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Applied Therapeutics, Inc.

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FY2022 Annual Report · Applied Therapeutics, Inc.
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UNITED STATES
SECURITIES AND EXCHANGE COMMISSION

Washington, D.C. 20549
FORM 10-K

(Mark One)

☒ ANNUAL REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the fiscal year ended December 31, 2022

OR

☐ TRANSITION REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the transition period from                    to

Commission file number 001-38898

Applied Therapeutics, Inc.

(Exact name of registrant as specified in its charter)

Delaware
(State or Other Jurisdiction of Incorporation or Organization)

81-3405262
(I.R.S. Employer Identification No.)

545 Fifth Avenue, Suite 1400, New York, NY

(Address of Principal Executive Offices)

10017

(Zip Code)

Registrant’s telephone number, including area code (212)-220-9226

Securities registered pursuant to Section 12(b) of the Act:

Title of each class

    Trading Symbol(s)

Name of each exchange on which registered

Common Stock $0.0001 par value

APLT

The Nasdaq Global Market

Securities registered pursuant to Section 12(g) of the Act: None

Indicate by check mark if the registrant is a well-known seasoned issuer, as defined in Rule 405 of the Securities Act. Yes ☐ No ☒

Indicate by check mark if the registrant is not required to file reports pursuant to Section 13 or Section 15(d) of the Act. Yes ☐ No ☒

Indicate  by  check  mark  whether  the  registrant  (1)  has  filed  all  reports  required  to  be  filed  by  Section  13  or  15(d)  of  the  Securities  Exchange  Act  of  1934  during  the
preceding 12 months (or for such shorter period that the registrant was required to file such reports), and (2) has been subject to such filing requirements for the past 90 days. Yes
☒ No ☐

Indicate by check mark whether the registrant has submitted electronically every Interactive Data File required to be submitted pursuant to Rule 405 of Regulation S-T

(§232.405 of this chapter) during the preceding 12 months (or for such shorter period that the registrant was required to submit such files). Yes ☒ No ☐

Indicate by check mark whether the registrant is a large accelerated filer, an accelerated filer, a non-accelerated filer, a smaller reporting company, or an emerging growth

company. See the definitions of “large accelerated filer,” “accelerated filer,” “smaller reporting company” and “emerging growth company” in Rule 12b-2 of the Exchange Act.

Large accelerated filer ☐     

Accelerated filer ☐     

Non-accelerated filer ☒

Smaller reporting company ☒ 

Emerging growth company ☒ 

If an emerging growth company, indicate by check mark if the registrant has elected not to use the extended transition period for complying with any new or revised

financial accounting standards provided pursuant to Section 13(a) of the Exchange Act. ☒

Indicate by check mark whether the registrant has filed a report on and attestation to its management’s assessment of the effectiveness of its internal control over financial

reporting under Section 404(b) of the Sarbanes-Oxley Act (15 U.S.C. 7262(b)) by the registered public accounting firm that prepared or issued its audit report. ☐

If securities are registered pursuant to Section 12(b) of the Act, indicate by check mark whether the financial statements of the registrant included in the filing reflect the

correction of an error to previously issued financial statements. ☐

Indicate by check mark whether any of those error corrections are restatements that required a recovery analysis of incentive-based compensation received by any of the

registrant’s executive officers during the relevant recovery period pursuant to §240.10D-1(b). ☐

Indicate by check mark whether the registrant is a shell company (as defined in Rule 12b-2 of the Exchange Act). Yes ☐ No ☒

The approximate aggregate market value of voting stock held by non-affiliates of the registrant, based upon the last sale price of the registrant’s common stock on the last
business day of the registrant’s most recently completed second fiscal quarter, June 30, 2022, as reported on The Nasdaq Global Market, was approximately $27,814,183. This
calculation excludes approximately 18,677,687 shares held by directors, executive officers and 10% or greater shareholders of the registrant. Exclusion of these shares does not
constitute a determination that each such person is an affiliate of the registrant.

As of March 22, 2023, the total number of shares outstanding of the registrant’s Common Stock was 48,113,561 shares, net of treasury shares.

Documents Incorporated by Reference: Portions of the registrant’s definitive proxy statement for the registrant’s 2023 annual meeting, to be filed within 120 days after

the close of the registrant’s fiscal year, are incorporated by reference into Part III of this Annual Report on Form 10-K.

    
    
    
APPLIED THERAPEUTICS, INC.
2022 FORM 10-K ANNUAL REPORT

TABLE OF CONTENTS

PART I

Table of Contents

Item 1. Business

Item 1A. Risk Factors

Item 1B. Unresolved Staff Comments

Item 2. Properties

Item 3. Legal Proceedings

Item 4. Mine Safety Disclosures

PART II

Item 5. Market for Registrant’s Common Equity, Related Stockholder Matters and Issuer Purchases of Equity
Securities

Item 6. Reserved

Item 7. Management’s Discussion and Analysis of Financial Condition and Results of Operations

Item 7A. Quantitative and Qualitative Disclosures About Market Risk

Item 8. Financial Statements and Supplementary Data

Item 9. Changes in and Disagreements with Accountants on Accounting and Financial Disclosure

Item 9A. Controls and Procedures

Item 9B. Other Information

Item 9C. Disclosure Regarding Foreign Jurisdictions that Prevent Inspections

Item 10. Directors, Executive Officers and Corporate Governance

Item 11. Executive Compensation

PART III

Item 12. Security Ownership of Certain Beneficial Owners and Management and Related Stockholder Matters

Item 13. Certain Relationships and Related Transactions, and Director Independence

Item 14. Principal Accountant Fees and Services

Item 15. Exhibits and Financial Statement Schedules

Item 16. 10-K Summary

PART IV

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CAUTIONARY NOTE REGARDING FORWARD-LOOKING STATEMENTS

This Annual Report on Form 10-K (this “Annual Report”) may contain “forward-looking statements” within the

meaning of the federal securities laws made pursuant to the safe harbor provisions of the Private Securities Litigation
Reform Act of 1995 about us and our industry that involve substantial risks and uncertainties. All statements other than
statements of historical fact contained in this Annual Report, including statements regarding our strategy, future financial
condition, future operations, projected costs, prospects, plans, objectives of management and expected market growth, are
forward-looking statements. In some cases, you can identify forward-looking statements by terminology such as “aim,”
“anticipate,” “assume,” “believe,” “contemplate,” “continue,” “could,” “design,” “due,” “estimate,” “expect,” “forecast,”
“goal,” “intend,” “may,” “objective,” “opportunity,” “plan,” “predict,” “project,” “positioned,” “potential,” “seek,”
“should,” “target,” “will,” “would” and other similar expressions that are predictions of or indicate future events and future
trends, or the negative of these terms or other comparable terminology.

We have based these forward-looking statements largely on our current expectations and projections about future
events and financial trends that we believe may affect our financial condition, results of operations, business strategy and
financial needs. These forward-looking statements are subject to a number of known and unknown risks, uncertainties and
assumptions, including risks described in the section titled “Risk Factors” in this Annual Report:

● our plans to develop, market and commercialize our product candidates;

● the initiation, timing, progress and results of our current and future preclinical studies and clinical trials and

our research and development programs;

● our ability to take advantage of expedited regulatory pathways for any of our product candidates;

● our estimates regarding expenses, future revenue, capital requirements and needs for additional financing;

● our ability to successfully acquire or license additional product candidates on reasonable terms and advance

product candidates into, and successfully complete, clinical studies;

● our ability to maintain and establish collaborations or obtain additional funding;

● our ability to obtain and timing of regulatory approval of our current and future product candidates;

● the anticipated indications for our product candidates, if approved;

● our expectations regarding the potential market size and the rate and degree of market acceptance of such

product candidates;

● our ability to fund our working capital requirements and expectations regarding the sufficiency of our capital

resources;

● the implementation of our business model and strategic plans for our business and product candidates;

● our intellectual property position and the duration of our patent rights;

● developments or disputes concerning our intellectual property or other proprietary rights;

● the potential impact of the Covid-19 pandemic on the timing and progress of our ongoing clinical trials, our
business, results of operations, liquidity, and operations and our ability to mitigate those potential impacts;

● our expectations regarding government and third-party payor coverage and reimbursement;

● our ability to compete in the markets we serve;

● the impact of government laws and regulations and liabilities thereunder;

● developments relating to our competitors and our industry; and

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● other factors that may impact our financial results.

The foregoing list of risks is not exhaustive. Other sections of this Annual Report include additional factors that

could harm our business and financial performance. Moreover, we operate in a very competitive and rapidly changing
environment. New risk factors emerge from time to time, and it is not possible for our management to predict all risk
factors nor can we assess the impact of all factors on our business or the extent to which any factor, or combination of
factors, may cause actual results to differ materially from those contained in, or implied by, any forward-looking
statements.

          In light of the significant uncertainties in these forward-looking statements, you should not rely upon forward-
looking statements as predictions of future events. Although we believe that we have a reasonable basis for each forward-
looking statement contained in this Annual Report, we cannot guarantee that the future results, levels of activity, 
performance or events and circumstances reflected in the forward-looking statements will be achieved or occur at all. You 
should refer to the sections titled “Risk Factors” and “Management’s Discussion and Analysis of Financial Condition and 
Results of Operations” for a discussion of important factors that may cause our actual results to differ materially from those 
expressed or implied by our forward-looking statements. Furthermore, if our forward-looking statements prove to be 
inaccurate, the inaccuracy may be material. Except as required by law, we undertake no obligation to publicly update any 
forward-looking statements, whether as a result of new information, future events or otherwise.

Unless the context otherwise requires, the terms “Applied,” “Applied Therapeutics,” “the Company,” “we,” “us,”

“our”, “the registrant” and similar references in this Annual Report on Form 10-K refer to Applied Therapeutics, Inc.

ITEM 1.       BUSINESS.

Overview

PART I

We are a clinical-stage biopharmaceutical company developing a pipeline of novel product candidates against

validated molecular targets in indications of high unmet medical need. We focus on molecules and pathways whose role in
the disease process is well known based on prior research, but have previously failed to yield successful products due to
poor efficacy and tolerability. Our unique approach to drug development leverages recent technological advances to design
improved drugs, employs early use of biomarkers to confirm biological activity and focuses on abbreviated regulatory
pathways. Our first molecular target is aldose reductase, or AR, an enzyme that converts glucose to sorbitol under oxidative
stress conditions, and is implicated in multiple diseases. Prior attempts to inhibit this enzyme were hindered by
nonselective, nonspecific inhibition, which resulted in limited efficacy and significant off-target safety effects. The
detrimental consequences of AR activation have been well established by decades of prior research. Our AR program
currently includes three small molecules, which are all potent and selective inhibitors of AR, but are engineered to have
unique tissue permeability profiles to target different disease states, including diabetic complications, heart disease and rare
metabolic diseases. The result of this unique multifaceted approach to drug development is a portfolio of highly specific
and selective product candidates that we believe are significantly de-risked and can move quickly through the development
process.

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AT-007 is a novel central nervous system, or CNS, penetrant ARI that we are developing for the treatment of rare 

metabolic diseases, including Galactosemia and Sorbitol Dehydrogenase (SORD) Deficiency.  Galactosemia is a 
devastating rare pediatric metabolic disease that affects how the body processes a simple sugar called galactose, and for 
which there is no known cure or approved treatment available. The U.S. Food and Drug Administration, or FDA, has 
granted both orphan drug designation and rare pediatric disease designation to AT-007 for the treatment of Galactosemia 
and in June 2021, the FDA granted Fast Track Designation to AT-007 for the treatment of Galactosemia. We have 
completed an adult study in healthy volunteers and Galactosemia patients, demonstrating that AT-007 is safe and well 
tolerated, and significantly reduces plasma galactitol levels vs. placebo. Galactitol is a toxic metabolite of galactose, which 
is formed in Galactosemia patients by aberrant activity of AR when galactose is present at high levels. A pediatric study is 
underway in children with Galactosemia, assessing the impact of AT-007 vs. placebo on safety, biomarker reduction of 
galactitol, and long-term functional outcomes. On April 13, 2021, we presented data featuring a cross-sectional analysis of 
nineteen pediatric patients with Classic Galactosemia, providing meaningful insight on the progressive worsening of the 
central nervous system phenotype with age. On October 18, 2021, we reported biomarker data from the pediatric ACTION-
Galactosemia Kids study. The results demonstrate a substantial reduction in plasma galactitol of approximately 40%, which 
was statistically significant (p<0.001) vs. placebo. We previously reported a baseline analysis of the 47 children enrolled in 
the study which demonstrated a clear correlation between baseline galactitol levels and baseline clinical functional 
outcomes. The long-term functional outcomes portion of the pediatric study is ongoing, and the outcomes are assessed 
every 6 months by a fire-walled data monitoring committee (DMC).  When the study reaches statistical significance in the 
active treated arm vs. the placebo arm, the DMC will alert the Company and the trial will be unblinded.  Statistical 
modelling suggests that this should occur at approximately the 18-month outcome assessment, based on currently available 
predictive information.  In April 2022, the Company met with the FDA to discuss the design of the ongoing pediatric study 
prior to the first 6-month outcomes assessment by the DMC.  The FDA confirmed that the pediatric study as it is currently 
designed would support an NDA submission if statistical significance is reached, and there is alignment between the FDA 
and the Company on the potential path forward to approval.  The 12-month clinical outcomes were assessed by the fire-
walled DMC, and as expected the data did not yet reach statistical significance, but demonstrated a trend in clinical 
outcomes favoring AT-007 vs. placebo.  A safety analysis showed that AT-007 continued to be safe and well tolerated.   
The Company is exploring a potential submission for conditional approval based on existing data with the European 
Medicines Agency (EMA).  

AT-007 is also being studied in a rare disease caused by deficiency in the enzyme Sorbitol Dehydrogenase, called 

SORD Deficiency. AR is the first enzyme in the polyol pathway, converting glucose to sorbitol. AR is then followed by 
Sorbitol Dehydrogenase, which converts sorbitol to fructose. Patients with SORD Deficiency accumulate very high levels 
of sorbitol in their cells and tissues as a result of the enzyme deficiency, which results in tissue toxicities such as peripheral 
neuropathy and motor neuron disease. Recent research in drosophila and cell models of SORD Deficiency demonstrated 
that treatment with an ARI that blocks sorbitol production may provide benefit in this disease. Preclinical studies on AT-
007 have demonstrated significant reduction in sorbitol levels in fibroblasts from SORD deficient patients. Treatment with 
AT-007 in the drosophila model of SORD  prevented the disease phenotype and protected from neuronal degeneration. On 
October 25, 2021, we reported data from a pilot open-label study in 8 SORD Deficiency patients. AT-007 reduced blood 
sorbitol levels by approximately 66% from baseline through 30 days of treatment. AT-007 was safe and well tolerated in all 
treated patients. In December 2021, we initiated a Phase 2/3 registrational study in patients with SORD Deficiency, which 
is ongoing at multiple clinical sites in the US and Europe. On February 16, 2023, we announced that in a pre-specified 
interim analysis of the ongoing Phase 3 INSPIRE trial, AT-007 reduced sorbitol levels by a mean of approximately 52% (or 
approximately 16,000ng/ml) over 90 days of treatment (p<0.001 vs. placebo) in patients with SORD Deficiency. At 
baseline, the mean blood sorbitol level of SORD patients included in this interim analysis was approximately 29,000ng/ml, 
with a range of approximately 22,000ng/ml-38,000ng/ml. In the INSPIRE trial, a baseline cross-sectional analysis of the 
relationship between sorbitol level, age (or duration of disease) and clinical outcome measures demonstrated a statistically 
significant correlation between sorbitol level and key clinical outcome measures, including 10-meter-walk/run speed, 4-
stair climb speed, and sit-to-stand test (p<0.05). The Company is working with the FDA to determine the appropriate 
regulatory path forward, as well as data required for an NDA submission, to advance AT-007 towards registration for this 
indication. The INSPIRE study will continue in blinded format to the 12-month interim clinical outcomes assessment. If 
the primary clinical outcome measure (10-meter-walk/run) reaches statistical significance at 12 months, the study will be 
completed and unblinded. If not, the study will continue in blinded format to 24 months, where clinical outcomes will be 
assessed again in a final statistical analysis. AT-007 continues to be safe and well tolerated to date.

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We also plan to initiate a clinical development program on AT-007 in another pediatric rare disease, called PMM2-
CDG. PMM2-CDG is a glycosylation disorder caused by deficiencies in the enzyme phosphomannomutase 2, which leads 
to CNS symptoms similar to Galactosemia, including low IQ, tremor, and speech and motor problems.  AR is over-
activated in this disease as a compensatory consequence of PMM2 deficiency, and a CNS penetrant ARI may be a 
compelling clinical option. Initial data in fibroblast cell lines derived from PMM2-CDG patients demonstrates that AT-007 
treatment increases phosphomannomutase 2 activity. A young child with PMM2-CDG is being treated in a single-patient 
investigator initiated trial with AT-007 at the University of North Carolina School of Medicine. Data has been presented at 
medical conferences in  2022  supporting a favorable treatment effect of AT-007 on biomarkers and organ function in this 
patient.  The FDA has granted pediatric rare disease designation and orphan designation for AT-007 in PMM2-CDG. 

In January 2023 we announced a partnership with Advanz Pharma for commercialization of AT-007 (govorestat) 
in Europe, and entered into an Exclusive License and Supply Agreement with Advanz Pharma (the Advanz Agreement).   
Advanz Pharma is a pharmaceutical company with a strategic focus on commercialization of specialty, hospital, and rare 
disease medicines in Europe.  Under the terms of the Advanz Agreement, Advanz Pharma receives exclusive commercial 
rights in the European Economic Area, Switzerland, and the UK for AT-007 in Galactosemia and SORD Deficiency, with 
certain rights to future indications for AT-007 in Europe.  We will receive certain near-term development milestone 
payments upon clinical trial completion and marketing authorization in Europe as well as commercial sales milestones, 
which in the aggregate amount to over €130 million, including €10 million upfront, which was paid upon signing. We will 
also receive royalties on any future net sales of AT-007 in Europe of 20%.  We will continue to be responsible for the 
development, manufacturing and supply of AT-007, and Advanz Pharma will be responsible for packaging, distribution and 
commercialization in Europe.

AT-001 is a novel ARI with broad systemic exposure and peripheral nerve permeability that we are developing for
the treatment of diabetic cardiomyopathy, or DbCM, a fatal fibrosis of the heart, for which no treatments are available. We
completed a Phase 1/2 clinical trial evaluating AT-001 in approximately 120 patients with type 2 diabetes, in which no
drug-related adverse effects or tolerability issues were observed. In September 2019, we announced the initiation of a
Phase 3 registrational trial of AT-001 in DbCM. The study, called ARISE-HF, is designed to evaluate AT-001’s ability to
improve or prevent the decline of functional capacity in patients with DbCM at high risk of progression to overt heart
failure. Although we did experience enrollment delays in 2020 associated with the Covid-19 pandemic, modifications were
made to the trial to include additional sites and geographies to address Covid-19-related issues. The trial is now fully
enrolled with 675 patients.

AT-003 is a novel ARI designed to cross through the back of the eye when dosed orally, and has demonstrated

strong retinal penetrance, for the treatment of diabetic retinopathy, or DR. DR is an ophthalmic disease that occurs in
diabetic patients and for which treatments are currently limited to high-cost biologics requiring intravitreal administration.
DR has been linked to AR activity, including elevations in sorbitol and subsequent changes in retinal blood vessels, which
distorts vision and leads to permanent blindness.

AT-104 is a preclinical dual selective PI3K inhibitor.  Due to recent regulatory changes impacting development of 
the PI3K inhibitor class of compounds, the Company has discontinued its early stage preclinical PI3K program and further 
development of AT-104. The compound and all rights associated with the technology were returned to Columbia
University.

Since inception in 2016, our operations have focused on developing our product candidates, organizing and

staffing our company, business planning, raising capital, establishing our intellectual property portfolio and conducting
clinical trials. We do not have any product candidates approved for sale and have not generated any revenue.

We have incurred significant operating losses since inception in 2016. Our ability to generate product revenue

sufficient to achieve profitability will depend on the successful development and commercialization of one or more of our
product candidates. Our net loss was $82.5 million for the year ended December 31, 2022. As of December 31, 2022, we
had an accumulated deficit of $348.8 million. We expect to continue to incur significant expenses and increasing operating
losses for the foreseeable future in connection with our ongoing activities. Furthermore, we expect

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to incur additional costs associated with operating as a public company, including significant legal, accounting, investor
relations and other expenses. As of December 31, 2022, we had cash and cash equivalents and short-term investments of
$30.5 million.

Our management team and scientific advisory board are composed of accomplished scientists and clinicians with decades
of experience developing drugs for a wide range of diseases. Our view is that drug development does not always need to
follow the standard approach, which often requires long and costly development programs before drugs become available
to patients. By taking a unique and focused approach to drug development, we believe we can significantly shorten
development programs and bring lifesaving drugs to patients in urgent need. In May 2019, we completed our initial public
offering (the “IPO”) whereby we sold 4,000,000 shares of common stock at a public offering price of $10.00 per share,
resulting in aggregate net proceeds of $34.6 million, after deducting underwriting discounts and commissions and offering
expenses. In November 2019, we completed a private placement of 1,380,344 shares of our common stock (the “Private
Placement”), which resulted in net proceeds of approximately $18.4 million. In January 2020, we completed a secondary
public offering of 2,471,489 shares of our common stock, including 411,223 shares sold pursuant to the underwriters’ full
exercise of their option to purchase additional shares (the “Secondary Public Offering”), pursuant to which we received
$134.1 million of proceeds, net of underwriting discounts and commissions and offering expenses. In February 2021, we
issued and sold 3,000,000 shares of common stock (the 
“February Offering”) at a public offering price of $23.00 per share, with an additional 450,000 shares sold pursuant to the 
underwriters’ full exercise of their option to purchase additional shares in the February Offering.  We received aggregate 
net proceeds, net of underwriting discounts and commissions and offering costs of $74.4 million. In June 2022, we 
completed an underwritten public offering of 20,000,000 shares of our common stock, par value $0.0001 per share, 
10,000,000 Pre-Funded Warrants, and accompanying Common Warrants to purchase up to 30,000,000 shares of our 
common stock. The shares and accompanying Common Warrants were offered at a price to the public of $1.00 per share 
and warrant, and the Pre-Funded Warrants and accompanying Common Warrants were offered at a price to the public of 
$0.9999, resulting in aggregate net proceeds of approximately $27.8 million, after deducting underwriting discounts and 
commissions and offering expenses.

We are actively pursuing several potential financing options. While we continue to explore opportunities to raise

additional equity capital in the public markets, this has proven to be challenging in the biotech sector recently. Other
options for structured finance which we continue to explore include a PIPE, debt, convertible debt, and synthetic royalty
financing. Synthetic royalty financing, in particular, has become a favorable option for many companies for funding
ongoing clinical development in late-stage and pre-approval programs. We have engaged an investment bank and we are
specifically exploring this option in the near term. Additionally, we are in active dialogue with several potential partners
regarding business development opportunities related to one or more of our programs. There can be no assurances that our
discussions with any of the current counterparties will be successful, and the Company expects to continue to pursue
additional opportunities.

Our Strategy

Our goal is to bring potentially transformative therapies to market across a range of fatal or debilitating diseases

for which no treatments are available. The critical components of our strategy include:

● Leveraging our unique approach to develop our pipeline of novel ARIs. We target molecules and pathways
that have a proven role in disease, but have previously failed to yield successful products due to poor efficacy
and tolerability. Our unique approach to drug development utilizes recent technological advances to design
improved drugs, employs early use of biomarkers to confirm biological activity and focuses on abbreviated
regulatory pathways. We develop product candidates with increased potency and selectivity by leveraging
recent technological advances in high throughput crystallography and in silico structural design. Our strategy
is also informed by early use of biomarkers to confirm biological activity and target engagement. Early proof
of biological activity through biomarkers in clinical trials combined with data from prior clinical
development programs on first generation drugs significantly de-risks clinical development in our target
indications. AR is our first molecular target that has been implicated in multiple diseases and for which
sorbitol levels can be assessed as a biomarker of enzyme activity. Prior AR-targeting compounds produced
nonselective inhibitors and failed to demonstrate adequate safety and

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efficacy. We intend to apply our strategy to a wide range of validated targets across multiple disease
indications, which we believe will result in additional pipeline programs.

● Rapidly advancing the development of our ARI product candidates, AT-007, AT-001 and AT-003.

Registrational studies for AT-007 in pediatric Galactosemia and SORD Deficiency and for AT-001 for the
treatment of DbCM are ongoing.

● Taking advantage of regulatory pathways designed for accelerated drug development in indications with
high unmet need and seeking strategic partnerships in other indications. We plan to leverage abbreviated
development programs and biomarker-based approaches for rapid drug development and regulatory approval
where possible. For indications that require standard development programs, we plan to seek strategic
partnerships.

● Expanding our pipeline to products targeting other validated molecules and pathways outside of AR. We

will continue leveraging our relationships with academic institutions and universities to acquire or license
additional technologies that are consistent with our strategy of applying new technologies to validated
molecular pathways.

Our Pipeline

The following table shows the status of our current ARI and PI3K inhibitor programs:

We seek to protect our proprietary and intellectual property position for our product candidates, our core
technology, and other know-how through U.S. and foreign patent protection. To the extent that our platform is not
patentable, we rely on trade secret protection and confidentiality agreements to protect our interests. For more information,
see the section titled “Business — Intellectual Property.”

Our Product Candidates

Our Aldose Reductase Program

AR is the first enzyme and rate-limiting step in the polyol pathway, an alternative glucose metabolism pathway.

AR is a redox-regulated enzyme that is activated by an altered redox state within the cell, which occurs during
hyperglycemia and ischemia. AR activation is associated with downstream consequences of hyperglycemia, such as
diabetic complications, as well as consequences of ischemia in the heart, such as acute myocardial infarction and chronic

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heart failure. As shown in the figure below, AR activity produces excess sorbitol, which causes osmotic dysregulation
within cells and tissues, such as nerve and retina, and is toxic to many cell types, including cardiomyocytes. Sorbitol is also
further metabolized to fructose, which initiates a cascade of metabolic dysregulation and inflammatory damage to cells,
such as: reactive oxygen species, or ROS, generation; advanced glycation end products, or AGE; protein kinase C, or PKC,
activation; and methylglyoxal overproduction. Under non-oxidative, or healthy patient conditions, AR remains largely
inactive and less than 3% of a healthy person’s glucose is processed by the polyol pathway. However, when the oxidative
environment of the cell changes due to hyperglycemia or ischemia, AR is both activated and upregulated, and greater than
30% of the patient’s glucose is then shunted through the polyol pathway, resulting in significant downstream damage to
cells and tissues. The detrimental consequences of AR activation have been well established by decades of prior research.
These include broad effects, such as mitochondrial dysfunction and cell death, as well as tissue-specific changes, such as
neuronal degeneration in peripheral nerves, collagen crosslinking and fibrosis in cardiac tissue, and damage to blood
vessels in the lens of the eye.

AR Causes Damage to Tissues Under Conditions of Oxidative Stress

* NF-kB is a protein complex that controls transcription of DNA, cytokine production and cell survival.

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Additionally, as shown in the figure below, abnormal AR activity is associated with conversion of galactose to

galactitol in patients with Galactosemia. Galactitol, like sorbitol, does not cross the cell membrane and causes damage to
cells across a wide range of tissues, including neurons in the brain, retinal cells in the eye and peripheral nerve tissue.

Galactitol Accumulation Results in Tissue Specific Damage

*     GALK, or galactokinase, and GALT, or galactose-1-phosphate uridyl transferase, are enzymes that metabolize

galactose.

**   Galactose-1-phosphate is referred to as Gal-1P.

During the 1980s and 1990s, AR was a significant target of drug development due to its established role in a wide

range of debilitating indications. Although these programs failed to produce effective drugs with a favorable risk/benefit
profile, the prior ARI clinical development programs validated the role of AR in the pathogenesis of several diabetic
complications and provided useful information on optimal patient criteria and trial design.

By applying new techniques in crystallography to better understand how the enzyme works, and applying in silico

design and medicinal chemistry approaches, we have developed compounds with logarithmically improved potency and
increased selectivity. Our technology includes specific compounds that are in various stages of preclinical and clinical
development, and is coupled with an understanding of how the enzyme works and a knowledge base of structural
approaches to drug the target while controlling drug characteristics, such as PK, solubility and tissue permeability.

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The following table summarizes the current status of our AR program and compound differentiation:

(1) IC50 is the amount of a compound required to inhibit 50% of enzyme activity.

(2) LogD is a log of partition of a chemical compound between the lipid and aqueous phases. LogD often predicts retinal

permeability, with compounds with negative LogD passing through the back of the eye.

AT-007 for the Treatment of Rare Metabolic Disease (Galactosemia, SORD Deficiency, PMM2-CDG)

Overview

AT-007 is a novel CNS penetrant ARI for the treatment of CNS rare diseases, including Galactosemia, SORD 

deficiency and PMM2-CDG.  

Galactosemia

Galactosemia is a devastating rare pediatric metabolic disease that affects how the body processes a simple sugar

called galactose, and for which there is no known cure or approved treatment available. High levels of galactose circulating
in the blood and tissues of Galactosemia patients enable AR to convert galactose to a toxic metabolite, galactitol, which
results in long-term complications ranging from CNS dysfunction to cataracts. AT-007 was specifically designed to be  
CNS penetrant to address AR activity in the brain and potentially prevent CNS consequences of the disease. We have 
demonstrated that treatment with AT-007 in an animal model of Galactosemia reduces toxic galactitol levels and prevents 
disease complications. We have also demonstrated that in patients with Galactosemia, plasma galactitol level statistically 
correlates with disease severity (p=0.004), further supporting the role of toxic galactitol in causing long-term disease 
complications. In adult and pediatric Galactosemia patients, we have demonstrated that AT 007 treatment resulted in a 
statistically significant reduction in plasma galactitol versus placebo. A pediatric long-term clinical study is underway.

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Diagnosis and Standard of Care

Galactosemia is caused by severe deficiency in the GALK or GALT enzymes that metabolize galactose. Galactose

is a sugar produced endogenously by the body, and is also a metabolite of lactose. Galactosemia is often fatal in infants
within the first weeks of life if they are exposed to dietary lactose in the form of breast milk or dairy-based formula. As
such, there is mandatory newborn screening for Galactosemia in the United States and many countries in Europe. While
prompt identification of infants with Galactosemia and immediate implementation of a lactose-restricted diet prevents
many fatalities, long-term consequences of disease persist due to endogenous generation of galactose within the body. We
are specifically developing AT-007 for patients with severe enzyme deficiencies in GALK, which is referred to as type 2
Galactosemia, and GALT, which is referred to as classic Galactosemia. In these patients, despite dietary restriction,
Galactosemia manifests as a combination of CNS and systemic toxicities in tissues, including cognitive dysfunction and
intellectual deficiencies, speech and motor pathologies, pre-senile cataracts and tremor, as well as ovarian insufficiency in
females.

There are no treatments available for Galactosemia. Due to endogenous production of galactose within the body,
infants with Galactosemia develop significant complications even with immediate implementation of, and strict adherence
to, a dairy-free diet. CNS complications include cognitive impairment, low IQ, speech and motor deficiencies, and
seizures. In addition, nearly all females develop ovarian insufficiency. Further to the damage that occurs in childhood,
many adults also develop persistent cataracts, seizures, and experience progressive worsening of tremor, cognitive,
behavioral and psychiatric issues due to ongoing tissue deposition of galactitol.

AR Activity Causes Toxic Accumulation of Galactitol in Galactosemia

We have demonstrated that inhibiting AR activity shifts galactose metabolism to an alternative enzyme called

galactose dehydrogenase, which allows galactose to be metabolized to galactonate, a benign substance that is removed in
the urine.

Market Opportunity

The global incidence of Galactosemia is estimated to be 1 in 50,000 to 1 in 90,000, depending on ethnicity. The

U.S. Galactosemia population is approximately 3,000 patients, based on newborn screening data identifying

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2,500 infants through 2014, and the estimated birth rate of 80 patients per year. Prior studies estimated that the U.S.
Galactosemia population was higher based on the incidence rates, because they did not take into account that, prior to
newborn screening, most infants with Galactosemia died within a few weeks of birth. As a result, the disease prevalence is
significantly lower, and the live population with Galactosemia is largely age 40 and younger. The EU population (including
the UK) is slightly larger than the US population, estimated at approximately 4,000 patients, leading to a combined US +
EU market opportunity of approximately 7,000 patients. When additional markets, such as Japan and Canada are
considered, we believe the overall Market opportunity for Galactosemia is approximately 7,600 patients worldwide.

Preclinical Studies

A rat model of classic Galactosemia displays similar biochemical and functional abnormalities to those associated

with Galactosemia in humans.

Treatment with AT-007 significantly reduced galactitol levels in target tissues, including blood, brain and liver,

without increasing galactose or Gal-1P levels, and prevented complications associated with galactitol accumulation in
tissues, including cataract formation and CNS dysfunction. The effects of AT-007 were dose dependent and corresponded
with galactitol reduction.

Clinical Development

ACTION-Galactosemia Phase 1/2 Study

We have evaluated AT-007 in a pivotal Phase 1/2 clinical trial in healthy volunteers and adults with Galactosemia.

The Phase 1 portion of the study in healthy volunteers evaluated safety, tolerability, CNS penetrance and PK of AT-007 at
doses of 5mg/kg to 40mg/kg for up to seven days of consecutive treatment. The Phase 2 portion in adults with
Galactosemia evaluated safety, tolerability, PK and pharmacodynamic reduction in the biomarker galactitol. Patients
received AT-007 5mg/kg, 20mg/kg, 40mg/kg or placebo, for 28 days.

AT-007 treatment resulted in a statistically significant and robust reduction in plasma galactitol versus placebo in
adult Galactosemia patients. Reductions in galactitol were dose dependent, with higher concentrations of AT-007 resulting
in a greater magnitude of reduction in galactitol. At the higher doses tested (20mg/kg and 40mg/kg), AT-007 significantly 
reduced plasma galactitol by approximately 50% from baseline.  Results were statistically significant (p value of less than 
0.01) vs. placebo. Galactitol reduction was rapid and sustained over time. No substantial change from baseline was 
observed in placebo treated patients. AT-007 was well tolerated in both Galactosemia patients and healthy volunteers.

ACTION-Galactosemia Kids

In June 2020, we initiated the ACTION-Galactosemia Kids pediatric Galactosemia study. The study was placed
on partial clinical hold in August 2020 while we worked with the FDA to redesign and operationally modify the study to
seamless design to ensure continuous treatment and the opportunity to receive clinical benefit. The study re-started in
February 2021 and is currently ongoing. The pediatric clinical trial is a 2-part study to evaluate safety, pharmacokinetics,
and reduction in the toxic biomarker, galactitol (Part A), as well as impact on functional outcomes in children with
Galactosemia over time (Part B). Three age cohorts are being studied in parallel: age 2-6, age 7-12, and age 13-17. An
additional cohort of children under 2 years of age may be added following analysis of safety data from the initial pediatric
cohorts. We have completed the biomarker portion of the study, demonstrating a 40% reduction in plasma galactitol
(p<0.001 vs. placebo). The clinical outcomes portion of the study is ongoing, evaluating the impact of AT-007 on how
patients feel and function over time.

While we had initially planned to submit an NDA for Accelerated Approval based on galactitol reduction, the 

FDA has since communicated that clinical outcomes data will be required for approval. The long-term functional outcomes 
portion of the pediatric study is ongoing, and the outcomes are assessed every 6 months by a fire-walled data monitoring 
committee (DMC).  When the study reaches statistical significance in the active treated arm vs. the placebo 

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arm, the DMC will alert the Company and the trial will be unblinded.  Based on discussions with the FDA, the Company 
believes  that the pediatric study as it is currently designed would support an NDA submission if statistical significance is 
reached.  The 12-month clinical outcomes were assessed by the fire-walled DMC, and as expected the data did not yet 
reach statistical significance, but demonstrated a trend in clinical outcomes favoring AT-007 vs. placebo.  A safety analysis 
showed that AT-007 continued to be safe and well tolerated.   The Company is exploring a potential submission for 
conditional approval based on existing data with the European Medicines Agency (EMA). 

SORD Deficiency

SORD Deficiency is a newly characterized genetic cause of Charcot-Marie-Tooth Type 2 Disease (“CMT2”) and 

distal hereditary neuropathy, in which patients are deficient in the enzyme Sorbitol Dehydrogenase (“SORD”). SORD is 
the enzyme which follows AR in the polyol pathway and converts sorbitol to fructose. Patients who are deficient in SORD 
can’t metabolize sorbitol normally, and sorbitol levels accumulate to unnaturally high levels.  Sorbitol, like galactitol, has 
been shown to be toxic to cells, especially neurons, resulting in progressive neuronal degeneration. Patients with SORD 
Deficiency develop progressive neuropathy, which greatly impacts mobility and motility, and significantly affects quality 
of life. 

Diagnosis and Standard of Care

Currently, patients with SORD Deficiency are diagnosed based on neurological symptoms and confirmatory 

genetic testing, which is available through several commercial labs and hospital systems.  There are currently no drugs 
approved to treat SORD Deficiency.

Market Opportunity

Genetic studies indicate that approximately 7-9% of CMT2 cases are caused by SORD Deficiency, estimating the

US population around 3,300 patients. The EU population (including the UK) is estimated to be approximately 4,400
patients. When additional markets, such as Japan and Canada are considered, we believe the overall Market opportunity for
Galactosemia is approximately 8,400 patients worldwide.

Preclinical Studies

Substrate reduction through AR inhibition in patient fibroblasts and a drosophila model of disease have
demonstrated preclinical proof of concept in SORD Deficiency, significantly reducing sorbitol levels and normalizing the
drosophila disease phenotype. Preclinical studies in fibroblasts derived from SORD Deficiency patients have demonstrated
significant reduction in sorbitol levels with AT-007 treatment. Preclinical studies in the drosophila model of disease have
demonstrated a positive impact on the disease phenotype with AT-007 treatment, including mobility (climbing) and
prevention of neuronal degeneration.

Clinical Development

In 2021 we conducted an open-label pilot study in 8 patients with SORD Deficiency.  AT-007 treatment 
significantly reduced sorbitol levels by approximately 66% from baseline, and was safe and well tolerated. In December 
2021 we initiated a Phase 2/3 registrational study in patients with SORD Deficiency. The registrational study, called the 
INSPIRE trial, is designed to demonstrate biomarker efficacy at 3 months through reduction in sorbitol, and long-term 
clinical efficacy over 2 years of treatment, with an interim clinical outcomes assessment at 12 months. The study is a 
multicenter placebo controlled trial conducted in the US and Europe in approximately 50 SORD patients age 16 and older. 
On February 16, 2023, we announced that in a pre-specified interim analysis of the ongoing Phase 3 INSPIRE trial, AT-007 
reduced sorbitol levels by a mean of approximately 52% (or approximately 16,000ng/ml) over 90 days of treatment 
(p<0.001 vs. placebo) in patients with SORD Deficiency. At baseline, the mean blood sorbitol level of SORD patients 
included in this interim analysis was approximately 29,000ng/ml, with a range of approximately 22,000ng/ml-38,000ng/ml. 
In the INSPIRE trial, a baseline cross-sectional analysis of the relationship between sorbitol level, age (or duration of 
disease) and clinical outcome measures demonstrated a statistically significant correlation between sorbitol level and key 
clinical outcome measures, including 10-meter-walk/run speed, 4-stair climb speed, and sit-to-stand test 

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(p<0.05). The Company is working with the FDA to determine the appropriate regulatory path forward, as well as data 
required for an NDA submission,  to advance AT-007 towards registration for this indication.  The INSPIRE study will 
continue in blinded format to the 12-month interim clinical outcomes assessment. If the primary clinical outcome measure 
(10-meter-walk/run) reaches statistical significance at 12 months, the study will be completed and unblinded. If not, the 
study will continue in blinded format to 24 months, where clinical outcomes will be assessed again in a final statistical 
analysis. AT-007 continues to be safe and well tolerated to date. 

PMM2-CDG

PMM2-CDG is a glycosylation disorder in which patients have only partial function of the phosphomannomutase

enzyme (“PMM2”). As a result, patients do not process sugars properly to support protein glycosylation, which results in
systemic problems and multi-organ failure. PMM2-CDG is a severe disease, resulting in and high mortality in children,
with no FDA approved treatments. PMM2-CDG is an ultra-rare disease, with only approximately 1,000 patients identified
worldwide.

Recently, AR inhibition was demonstrated to positively impact protein glycosylation in PMM2-CDG patient

fibroblasts and a C. elegans model of disease. It is believed that AR inhibition results in increased protein glycosylation by
shifting the balance of sugar production to support PMM2 activity. In preclinical studies in PMM2-CDG patient
fibroblasts, AT-007 significantly improved PMM2 activity. Based on this data, we have received both Orphan Designation
and Pediatric Rare Disease designation from the FDA.

AT-001 for the Treatment of Diabetic Cardiomyopathy

Overview

We are developing AT-001, a novel ARI with broad systemic exposure and peripheral nerve permeability being
developed for the treatment of DbCM, a fatal fibrosis of the heart, for which no treatments are available. We completed a
Phase 1/2 clinical trial evaluating AT-001 in approximately 120 patients with type 2 diabetes, in which no drug-related
adverse effects or tolerability issues were observed. This trial also demonstrated target engagement and proof of biological
activity, as measured by reduction in sorbitol, a biomarker of AR activity and NTproBNP. A registrational Phase 2/3 study
in DbCM patients at high risk of progression to overt heart failure (ARISE-HF) is currently ongoing.

Diagnosis and Standard of Care

DbCM is a fatal fibrosis of the heart that occurs in both type 1 and type 2 diabetic patients, which leads to

decreased contractility and decreased heart function, eventually resulting in fulminant heart failure. DbCM is caused by
metabolic derangements in cardiomyocytes that result in cell death and fibrosis. AR activity has been shown to be a large
contributor to these metabolic derangements, and the downstream effect of AR activation is responsible for the
cardiomyocyte cell death and fibrosis. DbCM is diagnosed by increased weight of the heart and decreased contractility,
which are identified by echocardiographic screening, as well as by exclusion of other forms of heart disease.
Epidemiological studies have shown that approximately 17% to 24% of diabetic patients display DbCM in the absence of
any other forms of heart disease. These patients do not have hypertension, atherosclerosis, valvular heart disease or
ischemia, and the only cause of the cardiomyopathy is the underlying diabetes. Stages of DbCM range from asymptomatic,
or stage 1, to acute heart failure, or stage 4. Most patients are not diagnosed until stage 2, where symptoms manifest as
extreme shortness of breath during exercise, referred to as decreased exercise tolerance. Exercise tolerance in these patients
(as measured by maximum amount of oxygen a person can utilize during intense exercise known as peak VO2) is
approximately 25% lower than diabetic patients without DbCM, and decreases by an additional 30% as the patients
progress to overt heart failure in later stages of diseases. Patients quickly progress at a steady state of decline to stage 3,
which includes marked cavity dilation and severe limitations in daily activities. The final stage of DbCM, stage 4, is
represented by acute heart failure resulting in death. The current standard of care is to target glucose control in these
patients, as well as hemodynamic modulation of blood flow, through use of beta blockers and diuretics. Both approaches
are largely ineffective, and DbCM often results in death within five to ten years of diagnosis. Approximately 24% of
DbCM patients progress to overt heart failure or death within 1.5 years of diagnosis, and 37% within five years of
diagnosis.

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Market Opportunity

According to a retrospective epidemiological study, approximately 17% of patients suffering from diabetes
develop DbCM. A study completed in France that utilized echocardiographic screening estimates the proportion of diabetic
patients to develop DbCM at approximately 24%. The International Diabetes Foundation estimated that there were
approximately 451 million patients globally with diabetes in 2017, which is expected to increase to 693 million by 2045.
This includes 58.0 million diabetes patients in Europe in 2017, which is expected to increase to 67.0 million in 2045, and
46.0 million in North America, which is expected to increase to 62.0 million in 2045. Based on an estimated prevalence of
17% of diabetic patients who develop DbCM, we estimate that currently there are approximately 77.0 million patients with
DbCM globally, with approximately 8.0 million in North America and 10.0 million in Europe. Initially, our development
program will target patients at high risk of progression to overt heart failure, which we estimate constitute approximately
50% of all DbCM patients. We believe these patients represent a symptomatic population that is more likely to be
responsive to treatment.

Prior AR-Based Approaches to Treat DbCM

AR activity has been implicated as a strong contributing factor to pathogenesis in DbCM. Pfizer Inc. was
developing an ARI, Alond (zopolrestat), for the treatment of DPN and DbCM in a Phase 2 clinical trial that demonstrated
favorable outcomes on heart function in DbCM patients, but the clinical trial was discontinued due to an unfavorable
risk/benefit profile, with several patients experiencing liver toxicity and significant elevations in both aspartate
aminotransferase and alanine aminotransferase, which are enzymes central to identification of liver toxicity and damage. In
this trial, patients with early-stage DbCM were identified by echocardiographic screening and were randomized to three
treatment groups, which consisted of placebo, 500 mg zopolrestat per day or 1,000 mg zopolrestat per day dosed for one
year. Due to liver toxicity seen in another trial with zopolrestat, the 1,000 mg treatment arm was reduced to 500 mg, and
the two doses were collapsed into one treatment arm. While patients on placebo displayed decreased heart function over
the year of the trial as their disease progressed, patients on zopolrestat displayed a stabilization of heart function and even
improvement in heart function in some patients based on hemodynamic endpoints. We believe this data validates the
approach of using an ARI to improve outcomes for patients with DbCM and using our compounds, which demonstrate
improved potency and have been well tolerated, may lead to greater clinical utility.

We have demonstrated that when compared to zopolrestat, AT-001 has significantly higher in vitro enzymatic

inhibitory activity and greater specificity for AR. Liver toxicity associated with “old” ARIs such as zopolrestat has been
shown to be due to off-target inhibition of a structurally related enzyme, Aldehyde Reductase, which is required for normal
liver function. AT-001 demonstrates increased selectivity for AR, and does not inhibit Aldehyde Reductase at any
concentration tested. This increased selectivity led to lack of toxicity in cultured hepatocytes, or liver cells, whereas
zopolrestat demonstrated significant toxicity in hepatocytes. Thus, we believe that not only is AT-001 a more potent AR
inhibitor than prior drugs, but that we have overcome the safety and toxicity limitations from prior compounds, which were
due to lack of selectivity and off-target inhibition of Aldehyde Reductase.

Preclinical Efficacy Studies

In a preclinical model of DbCM AT-001 prevented cardiac damage and dysfunction and normalized cardiac

energetics. In a diabetic rat model, AT-001 prevented cardiac damage induced by ischemia/repurfusion.

Clinical Development

Until recently, development in cardiovascular disease indications often required large outcome-based trials that

examined survival and re-hospitalization as primary endpoints. These trials were extremely large, expensive and time-
consuming, and were often confounded by comorbidities in the patient population. As a result, very few cardiovascular
programs resulted in approved drugs. There has been a recent effort from the Division of Cardiovascular and Renal
Products at the FDA, as well as at the European Medicines Agency, or EMA, to streamline drug development for
cardiovascular disease to increase the probability of demonstrating a meaningful clinical effect in patients. Specifically, in
cardiomyopathies, where there is a direct functional link between hemodynamic endpoints, heart

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contractility and quality of life, there is a unique opportunity to demonstrate benefit of therapy in a smaller number of
patients and shorter treatment period than was previously required. Recent clinical development programs in hereditary
cardiomyopathies have pioneered smaller trials examining exercise tolerance and/or heart functional capacity as a primary
endpoint.

Consistent with these developments, at our pre-IND meeting, the FDA indicated that we would not be required to

examine survival and re-hospitalization endpoints, and confirmed that exercise tolerance would qualify as an appropriate
primary endpoint in our DbCM trial. This was also recently publicly confirmed by the FDA in a whitepaper entitled “Draft
Guidance for Industry: Treatment for Heart Failure: Endpoints for Drug Development.” Accordingly, we designed our
pivotal Phase 2/3 clinical trial to target functional capacity, or exercise tolerance, as measured by Peak VO2 on
Cardiopulmonary Exercise Testing (CPET) in DbCM patients at high risk of progression to overt heart failure.

Phase 1/2 Trial in Adult Type 2 Diabetic Patients

We have evaluated AT-001 in a placebo-controlled Phase 1/2 clinical trial in approximately 120 type 2 diabetes

patients. The primary objectives of this trial were to explore the safety, tolerability and PK profile of AT-001. Because AR
converts glucose to sorbitol, and AR activity is elevated in diabetic patients, sorbitol normalization was also examined as a
pharmacodynamic, or PD, biomarker of target engagement, which provided proof of biological activity in patients.

The Phase 1/2 clinical trial allowed use of concomitant treatments for glucose control, as well as other standard of
care treatments for diabetes, such as statins and ACE inhibitors. The FDA permitted us to directly evaluate diabetic patients
due to positive data from the preclinical studies, as well as the urgency to develop drugs quickly due to high unmet need.
AT-001 was dosed as an active pharmaceutical ingredient, or API, powder in a rapid release capsule and the trial examined
both once-daily and twice-daily, or BID, dosing regimens.

AT-001 was safe and well tolerated at all doses tested. Additionally, there were no observed adverse interactions
with any concomitant diabetes medications used by patients during the trial. Because AR converts glucose to sorbitol, and
AR activity is elevated in diabetic patients, sorbitol normalization to healthy subject levels can be used as a PD biomarker
of target engagement and proof of biological activity. Treatment with AT-001 normalized sorbitol levels in diabetic patients
to those of healthy volunteers, and prevented post-prandial elevations in sorbitol. Decrease in sorbitol levels was dose-
dependent, with higher doses of AT-001 resulting in greater reduction in sorbitol levels. Reduction in sorbitol levels lasted
for approximately 10-12 hours post dose, suggesting that twice-daily oral dosing produced optimal pharmacodynamic
impact. Placebo-treated patients did not demonstrate any reduction in sorbitol levels, and conversely demonstrated post-
prandial increase in sorbitol levels.

Within the Phase 1/2 study, approximately 30 patients with early stage DbCM, assessed by echocardiographic 

abnormalities and elevations in the cardiac stress biomarker, NTproBNP, were treated with AT-001 or placebo for 28 days.  
Treatment with AT-001 (twice daily or three times daily) resulted in sustained reduction in sorbitol, and significant 
reduction in NTproBNP, demonstrating that inhibition of AR decreases cardiac stress. This data supported dose selection 
and advancement into a Phase 2/3 registrational trial for DbCM.

In September 2019, we initiated a Phase 3 registrational trial for AT-001 in DbCM called ARISE-HF. ARISE-HF
is a global study, recruiting patients at sites in North America, Europe, Australia and Hong Kong. The primary endpoint of
the trial is stabilization or decrease in slope of decline on functional capacity, as measured by peak VO2, the rate of oxygen
consumption measured during exercise. We are also evaluating heart function by echocardiogram-based hemodynamic
endpoints, progression to overt heart failure, and quality of life, as well as biomarkers of heart inflammation and damage.
This trial consists of 675 patients in three cohorts of approximately 225 patients each, including a placebo group, a low
dose AT-001 group (1,000mg twice daily) and a high dose AT-001 group (1,500mg

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twice daily). The trial treatment period for evaluation of the primary endpoint is 15 months, with additional endpoints
evaluated at 27 months. The trial is fully enrolled and ongoing.

AT-001 for the Treatment of Diabetic Peripheral Neuropathy

Overview

We also intend to develop AT-001 for DPN, a debilitating neurodegenerative disease that significantly reduces

patients’ quality of life, and for which there are currently no FDA-approved treatments. We expect this indication will
require a standard clinical development path, and as such we plan to pursue a strategic partnership in order to expand into
this indication. Since many patients with DbCM also have DPN, we are collecting proof-of-concept data through our
DbCM program to support our efforts in our DPN program. We have included a DPN sub-study in our pivotal DbCM
study.

Diagnosis and Current Standard of Care

DPN is diagnosed by a simple neurological assessment, usually the Toronto Neuropathy Scoring System, which is

administered in the physician’s office and examines a patient’s ability to feel various types of neurological stimuli on the
hands and feet. AR activity has been shown to cause DPN. Epalrestat, an ARI, is approved in Japan, China and India to
prevent further neuronal degeneration in DPN patients. However, there are no disease modifying therapies approved in the
United States and Europe, and only symptomatic medications, such as Lyrica, are approved for pain associated with DPN.
Although epalrestat was approved in Japan in 1992 based on very limited clinical data that would not have been sufficient
for other markets, more recent academic studies have demonstrated an effect on MNCV and symptomatic pain endpoints in
a wide range of diabetic patients. For example, a multicenter, three-year Phase 3 clinical trial conducted in Japan on
epalrestat 150 mg versus placebo demonstrated that epalrestat prevented progression of DPN in diabetic patients versus
placebo. Epalrestat prevented degeneration of nerve function, as measured by MNCV, and prevented worsening of
symptomatic pain. A statistically significant effect was demonstrated in all patients regardless of low or high levels of
glucose attached to their hemoglobin, as tested by a hemoglobin A1C (HbA1C) test.

Epalrestat, which is now generic in Japan, reached peak sales of approximately $226 million in 2001. This is

indicative of its widespread use in the Japanese diabetic population, which was approximately five million patients at the
time of launch despite significant tolerability issues associated with use and five times daily dosing due to a very short half-
life. We do not believe, however, that it is likely to be a candidate for further commercialization. Nevertheless, prior
research on epalrestat evinces the role of AR in DPN and provides a clinical trial design to demonstrate efficacy in this
indication.

Market Opportunity

Approximately 50% of the global diabetic population, or 226 million diabetic patients, suffer from DPN, with
23.0 million patients in North America and 29.0 million patients in Europe. Due to availability of generic epalrestat in
China and India, we view the opportunity in these two markets to be limited as a result of pricing pressures and
differentiation requirements with regard to epalrestat. However, we believe a significant market opportunity for a more
effective ARI with a favorable dosing regimen still exists in Japan, a less price sensitive market where there is familiarity
with the mechanism of action in the disease and use of epalrestat is high. As such, although we are currently focused on the
U.S. market, we may expand our efforts into Japan opportunistically.

Preclinical Studies

In preclinical studies, AT-001 prevented neuronal degeneration in animal models of DPN, as measured by MNCV
in sciatic and tail nerves of diabetic rats. AT-001 treatment prevented peripheral neuronal damage, as measured by MNCV
after six weeks of treatment. A dose-dependent reduction in neuronal dysfunction was observed in rats treated

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with AT-001, and treatment at 30 mg/kg of AT-001 completely prevented neuronal degeneration, with no statistical
difference from non-diabetic WT rats.

Clinical Development

Since many DbCM patients often also suffer from DPN, we have incorporated DPN endpoints, such as MNCV, as

a sub-study into our DbCM ARISE-HF pivotal study to provide additional proof-of-concept for AT-001 in DPN. We plan
to seek a strategic partnership to develop AT-001 for treatment of DPN and advance the program into Phase 3 clinical trial
for this indication.

AT-003 for the Treatment of Diabetic Retinopathy

Overview

We are developing AT-003, an ARI designed to cross through the back of the eye when dosed orally, which has

demonstrated strong retinal penetrance, for the treatment of DR. DR is an ophthalmic disease that occurs in diabetic
patients, and for which treatments are currently limited to intravitreal administration. DR has been linked to AR activity,
including elevations in sorbitol and subsequent changes in retinal blood vessels, which distorts vision and leads to
permanent blindness. We are currently in late stages of preclinical development and intend to advance AT-003 into a
Phase 1 clinical trial for the treatment of DR.

Diagnosis and Current Standard of Care

DR is diagnosed by routine dilated eye exam by an ophthalmologist. Annual or biennial ophthalmic exams to

screen for DR are a recommended standard of care for diabetic patients under current treatment guidelines. Vascular
endothelial growth factor, or VEGF, inhibitors, Lucentis (ranibizumab) and Eylea (aflibercept), are approved to treat severe
or late-stage DR, but are limited by high cost, the need for intravitreal injection into the eye and the lack of therapeutic
benefit in many patients. A need exists for safe, effective and tolerable treatments for DR early in the disease process that
provide a benefit to a wide range of patients. AR is an attractive target for DR drug development since AR activity is
upstream of VEGF activity in DR pathogenesis. AR has been shown to cause DR by inducing hyperosmolarity in retinal
cells due to elevated sorbitol, as well as through fructose-mediated detrimental downstream effects, such as AGE
generation and PKC activation. AR knock-out rats are protected from DR development, and several prior ARIs
demonstrated efficacy on DR endpoints in clinical trials, but were not approved due to dose-limiting safety concerns.

Market Opportunity

A recent retrospective epidemiological analysis of diabetic patients globally confirmed that DR affects
approximately 35% of diabetics, and is a leading cause of blindness worldwide. Based on the 2017 diabetes numbers, the
global market for DR is approximately 158 million patients, with anticipated increase to 243 million by 2045. The current
market is approximately 16.0 million in North America and 20.0 million in Europe.

Preclinical Studies

AT-003 displayed significant retinal penetration when dosed orally in diabetic rats. AT-003 was observed to be

well tolerated over a seven-day dosing period in all doses tested, up to 1,000 mg/kg daily, with no adverse effects observed.
Efficacy of AT-003 is currently being explored in two animal models of DR — an ischemic injury model (acute damage)
and chronic diabetic treatment model.

Clinical Development Plan

Similar to AT-001, we plan to explore the safety, tolerability, PK profile and biomarker effects of AT-003 in a
Phase 1a/1b clinical trial in diabetic patients. Assuming positive data in this trial, we plan to initiate a pivotal Phase 2/3
clinical trial of AT-003 in patients with DR to prevent disease progression versus placebo, as measured by subjective

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metrics, including fluoroscein angiography and optical coherence tomography, which are scans used in the examination and
management of retinal diseases.

Exclusive License Agreement with Columbia University

On October 26, 2016, we entered into a license agreement with Columbia University (the “2016 Columbia
Agreement”). Pursuant to the 2016 Columbia Agreement, Columbia University granted us a royalty-bearing, sublicensable
license that is exclusive with respect to certain patents, and non-exclusive with respect to certain know-how, in each case to
develop, manufacture, and commercialize ARI products, including AT-001, AT-003 and AT-007. The license grant is
worldwide with the exception of a single patent family covering AT-001 and AT-003 for which the license grant excludes
China, Taiwan, Hong Kong and Macao. Under the 2016 Columbia Agreement, we are obligated to use commercially
reasonable efforts to research, discover, develop and market licensed products for commercial sale in the licensed territory,
and to comply with certain obligations to meet specified development and funding milestones within defined time periods.
Columbia University retains the right to conduct, and grant third parties the right to conduct, non-clinical academic
research using the licensed technology; provided that such research is not funded by a commercial entity or for-profit entity
or results in rights granted to a commercial or for-profit entity. As the technology licensed to us under the 2016 Columbia
Agreement was developed as a result of a U.S. government grant, the licenses granted to us under the agreement are
subject to the terms of such grant, and to standard rights of the U.S. government under the Bayh-Dole Act, including the
grant to the government of a non-exclusive, worldwide, freedom to operate license under any patents, and the requirement,
absent a waiver, to manufacture products substantially in the United States.

As consideration for entering into the 2016 Columbia Agreement, we made a nominal upfront payment to
Columbia University and, following the occurrence of certain trigger events, issued to Columbia University shares equal to
5% of our outstanding common stock on a fully diluted basis at the time of issuance. We will be required to make further
payments to Columbia University of up to an aggregate of $1.3 million for the achievement of specified development and
regulatory milestones, and up to an aggregate of $1.0 million for the achievement of a specified level of aggregate annual
net sales, in each case in connection with products covered by the 2016 Columbia Agreement. We will also be required to
pay tiered royalties to Columbia University in the low- to mid-single digit percentages on our, our affiliates’ and our
sublicensees’ net sales of licensed products, subject to specified offsets and reductions. In addition, we are required to
make specified annual minimum royalty payments to Columbia University in the mid six figures beginning on the
10th anniversary of the effective date of the agreement. When we grant sublicenses under the 2016 Columbia Agreement
we are required to pay to Columbia University a portion of the net sublicensing revenue received from such third parties, at
percentages between 10% and 20%, depending on the stage of development at the time such revenue is received from such
third parties. The Advanz Agreement includes a sublicense under the 2016 Columbia Agreement.

Columbia University is responsible for the prosecution and maintenance of the licensed patents, in consultation 
with us, and subject to a requirement to give due consideration to our comments, at our expense.  We have the first right, 
but not the obligation, to control the enforcement of licensed patents exclusively licensed to us against third parties. We are 
required to indemnify Columbia University for any third party claims that arise from or relate to the 2016 Columbia 
Agreement.

The 2016 Columbia Agreement will terminate upon the expiration of all our royalty payment obligations in all
countries. We may terminate the 2016 Columbia Agreement for convenience upon 90 days’ written notice to Columbia
University. At its election, Columbia University may terminate the 2016 Columbia Agreement, or convert the licenses
granted to us into non-exclusive, non-sublicensable licenses, in the case of (a) our uncured material breach upon 30 days’
written notice (which shall be extended to 90 days if we are diligently attempting to cure such material breach), (b) our
failure to achieve the specified development and funding milestone events, or (c) our insolvency. The 2016 Columbia
Agreement may not be assigned by us without Columbia University’s consent, except to any successor to all or
substantially all of our business to which the 2016 Columbia Agreement relates and upon notice to Columbia University.

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In January 2019, we entered into a second license agreement with Columbia University (the “2019 Columbia 

Agreement”). Pursuant to the 2019 Columbia Agreement, Columbia University granted us a royalty-bearing, sublicensable 
license that is exclusive with respect to certain patents, and non-exclusive with respect to certain know-how, in each case to 
develop, manufacture and commercialize PI3k inhibitor products.  The license grant is worldwide. Under the 2019 
Columbia Agreement, we are obligated to use commercially reasonable efforts to research, discover, develop and market 
licensed products for commercial sale in the licensed territory, and to comply with certain obligations to meet specified 
development and funding milestones within defined time periods. Columbia University retains the right to conduct, and 
grant third parties the right to conduct, non-clinical academic research using the licensed technology; provided that such 
research is not funded by a commercial entity or for-profit entity or results in rights granted to a commercial or for-profit 
entity. As consideration for entering into the 2019 Columbia Agreement, we made a nominal upfront payment to Columbia 
University. We will be required to make further payments to Columbia University of up to an aggregate of $1.3 million for 
the achievement of specified development and regulatory milestones, and up to an aggregate of $1.0 million for the 
achievement of a specified level of aggregate annual net sales, in each case in connection with products covered by the 
2019 Columbia Agreement. We will also be required to pay tiered royalties to Columbia University in the low- to mid-
single digit percentages on our, our affiliates’ and our sublicensees’ net sales of licensed products, subject to specified 
offsets and reductions. In addition, we are required to make specified annual minimum royalty payments to Columbia 
University, which is contingent upon the approval of the licensed products, in the mid-six figures beginning on the tenth 
anniversary of the effective date of the 2019 Columbia Agreement.

In July 2022, following regulatory changes impacting development of the class of PI3k inhibitors and the 

Company’s decision to discontinue its early stage preclinical PI3k program, the Company and Columbia entered into an 
agreement terminating the 2019 Columbia Agreement (the “2022 Columbia Termination Agreement”) as of July 25, 2022.   
Under the terms of the 2022 Columbia Termination Agreement, the Company assigned certain regulatory documents 
regarding the preclinical PI3k inhibitor AT-104 to Columbia and granted Columbia a non-exclusive royalty free license 
(with rights to sublicense any future Columbia licensee) under certain know-how, technical information and data relating to 
AT-104 that was developed by the Company during the term of the 2019 Columbia Agreement.

In March 2019, and in connection with the 2016 Columbia Agreement, the Company entered into a research

services agreement (the “2019 Columbia Research Agreement”) with Columbia University with the purpose of analyzing
structural and functional changes in brain tissue in an animal model of Galactosemia, and the effects of certain compounds
whose intellectual property rights were licensed to the Company as part of the 2016 Columbia Agreement on any such
structural and functional changes. The 2019 Columbia Research Agreement had a term of 12 months from its effective date
and expired in accordance with its terms.

On October 3, 2019, and in connection with the 2019 Columbia Agreement, the Company entered into a research
services agreement (the “PI3k Columbia Research Agreement” and collectively with the 2016 Columbia Agreement, 2019
Columbia Agreement and 2019 Columbia Research Agreement, the “Columbia Agreements”) with Columbia University
with the purpose of analyzing PI3k inhibitors for the treatment of lymphoid malignancies. The PI3k Columbia Research
Agreement had a term of 18 months from its effective date and expired in accordance with its terms.

License Agreement with University of Miami

On October 28, 2020, we entered into a license agreement (the “2020 Miami License Agreement”) with the 

University of Miami relating to certain technology that is co-owned by the University of Miami (UM), the University of 
Rochester (UR) and University College London (UCL Business Ltd. (UCL)). UM was granted an exclusive agency from 
UR and UCL to license each of their rights in the technology. Pursuant to the 2020 Miami License Agreement, UM, on 
behalf of itself and UR and UCL, granted us a royalty-bearing, sublicensable license that is exclusive with respect to 
certain patent applications and patents that may grant from the applications, and non-exclusive with respect to certain 
know-how, in each case to research, develop, make, have made, use, sell and import products for use in treating and/or 
detecting certain inherited neuropathies, in particular those caused by mutation in the sorbitol dehydrogenase (SORD) 
gene.  The license grant is worldwide. Under the 2020 Miami License Agreement, we are obligated to use commercially 
reasonable efforts to develop, manufacture, market and sell licensed products in the licensed territory, and to comply with 
certain obligations to meet specified development milestones within defined time periods. UM retains for itself UR 

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and UCL the right to use the licensed patent rights and licensed technology for their internal non-commercial educational, 
research and clinical patient care purposes, including in sponsored research and collaboration with commercial entities. As 
the technology licensed to us under the 2020 Miami License Agreement was developed as a result of a U.S. government 
grant, the licenses granted to us under the agreement are subject to the terms of such grant, and to standard rights of the 
U.S. government under the Bayh-Dole Act, including the grant to the government of a non-exclusive, worldwide, freedom 
to operate license under any patents, and the requirement, absent a waiver, to manufacture products substantially in the 
United States.

Under the terms of the 2020 Miami License Agreement, we are obligated to pay the University an up-front non-

refundable license fee of $1.1 million, and a second non-refundable license fee of $0.5 million due on the first anniversary
of the date of the license. We will be required to make further payments to UM of up to an aggregate $2.2 million for the
achievement of specified patenting and development milestones, and up to an aggregate of $4.1 million for achievement of
late stage regulatory milestones. We will also be required to pay royalties ranging from 0.88% - 5% on ours, our affiliates’
and our sublicensees’ net sales of licensed products. When we sublicense the rights granted under the 2020 Miami License
Agreement to one or more third parties, we are required to pay to UM a portion of the non-royalty sublicensing revenue
received from such third parties ranging from 15% – 25%. The Advanz Agreement includes a sublicense under the 2020
Miami License Agreement.

The  2020  Miami  License  Agreement  terminates  upon  the  expiration  of  all  issued  patents  and  filed  patent
applications  or  10  years  after  the  first  commercial  sale  of  the  last  product  or  process  for  which  a  royalty  is  due,  unless
earlier terminated. In addition, the 2020 Miami License Agreement may be terminated by us at any time upon 60 days prior
written notice to UM, and may be terminated by either us or UM upon material breach of an obligation if action to cure the
breach is not initiated within 60 days of receipt of written notice.

On October 28, 2020, we entered into an option agreement with the University of Miami (the “2020 Miami
Option Agreement”) concerning certain research activities and technology relating to SORD neuropathy that may be
pursued and developed by UM. Under the 2020 Miami Option Agreement, if UM conducts such research activities, then
UM is obligated to grant us certain option rights to access and use the research results and to obtain licenses to any
associated patent rights upon us making specified payments to UM within specified time limits. If we elect to obtain option
rights, we will be required to make payments to UM in the low-six figures to the low-seven figures, depending upon the
rights we elect to obtain, and we will be obligated to make certain milestone payments in the high-six figures to mid-seven
figures if UM conducts and completes certain research activities within specified time periods and we elect to receive
rights to use the results of that research.

On December 14, 2020, we entered into a research agreement with the University of Miami (the “2020 Miami 
Research Agreement”), pursuant to which the University of Miami agreed to conduct a research study relating to SORD 
neuropathy and deliver a final report on the study to us. The term of the research agreement was from December 14, 2020 
through December 30, 2021. The consideration for the 2020 Miami Research Agreement was $0.3 million. Due to COVID-
19 pandemic disruptions certain research under the 2020 Miami Research Agreement was not completed.  In January 2022, 
we amended the 2020 Miami Research Agreement to extend the term of the agreement to August 31, 2022.

License Agreement with Advanz Pharma

On January 3, 2023, we entered into an Exclusive License and Supply Agreement (the “ Advanz Agreement”)

with Mercury Pharma Group Limited (trading as Advanz Pharma Holdings). Pursuant to the Agreement, we granted
Advanz Pharma the exclusive right and license to commercialize drug products containing AT-007 (also known as
govorestat), our proprietary Aldose Reductase Inhibitor (ARI) (the “Licensed Product”), for use in treatment of Sorbitol
Dehydrogenase Deficiency (“SORD”) and Galactosemia (each a “Licensed Indication”) in the European Economic Area,
Switzerland and the United Kingdom (the “Territory”). We also granted Advanz Pharma a right of negotiation and “most-
favored nation” rights with respect to acquiring the European commercialization rights for any additional indications for
which the Licensed Product may be developed in the future (or any other products we may develop solely to the extent
used for the Licensed Indications).

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Advanz Pharma is required to use commercially reasonable efforts to launch and commercialize the Licensed

Products in the major markets in the Territory in each Licensed Indication following, and subject to, receipt of marketing
authorization therein. Under the Advanz Agreement, Advanz Pharma agreed to pay us (i) an upfront payment of EUR 10
million (approx. USD $10.7 million), and certain development milestone payments upon clinical trial completions and
receipt of marketing authorization in the territory, as well as certain commercial milestone payments, totaling EUR 134
million (approx. USD $142.2 million) in the aggregate, and (ii) royalties of 20% of net sales of the Licensed Product. Such
royalty rate will be payable on a country-by-country basis until the later of (i) the expiration of the licensed patents
covering the composition of matter of AT-007, or (ii) 10 years after the European Medicines Agency’s grant of marketing
authorization for the Licensed Product. The royalties are subject to certain deductions, including certain secondary
finishing costs, certain step-in establishment costs and a portion of fees for any potential third party patent licenses if
applicable in the future. Following the initial term of the license, as described above, the royalty rate shall be reduced to
10% and shall continue in perpetuity unless the Agreement is terminated in various circumstances in accordance with its
terms.

Certain of the patents licensed to Advanz Pharma under the Advanz Agreement are sub-licensed from the

University of Miami and Columbia University, and thus remain subject to certain obligations of the Company (including
royalty obligations) to such institutions. For more information on these arrangements see “—Exclusive License Agreement
with Columbia University” and “—License Agreements with the University of Miami.”

Sales and Marketing

Due to the delay in the anticipated Galactosemia commercial launch, external non-essential commercial
expenditures have been suspended, including sales and marketing, and we have recognized significant reductions in our
commercial spending during the year ended December 31, 2022.

Manufacturing

We do not own or operate, and currently have no plans to establish, any manufacturing facilities. We depend on
third party contract manufacturing organizations, or CMOs, for all of our requirements of raw materials, drug substance
and drug product for our preclinical research and our clinical trials for AT-007, AT-001 and AT-003. We have not entered
into long-term agreements with our current CMOs. We intend to continue to rely on CMOs for later-stage development and
commercialization of our current products, as well as the development and commercialization of any other product
candidates that we may identify. Although we rely on CMOs, we have personnel and third party consultants with extensive
manufacturing experience to oversee the relationships with our contract manufacturers.

We believe the synthesis of the drug substance for AT-007 and AT-001 are reliable and reproducible from readily

available starting materials, and the synthetic routes are amenable to large-scale production and do not require unusual
equipment or handling in the manufacturing process. We have obtained adequate supplies of the drug substance for AT-007
and AT-001 to satisfy our immediate clinical and preclinical demands.

Drug product formulation development for AT-007 and AT-001 are in progress. We have contracted with a third

party manufacturer capable of both formulation development and drug product manufacturing through commercialization.
We may identify a second drug product manufacturer in the future to add additional capacity and redundancy to our supply
chain.

Competition

The pharmaceutical industry is characterized by rapidly advancing technologies, intense competition and a strong
emphasis on proprietary products. While we believe that our technology, the expertise of our executive and scientific team,
research, clinical capabilities, development experience and scientific knowledge provide us with competitive advantages,
we face potential competition from many different sources, including pharmaceutical and biotechnology companies,
academic institutions and governmental agencies and public and private research institutions.

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Product candidates that we successfully develop and commercialize may compete with existing therapies and new
therapies that may become available in the future.

Our competitors may have significantly greater financial resources, established presence in the market, expertise

in research and development, manufacturing, preclinical and clinical testing, obtaining regulatory approvals and
reimbursement and marketing approved products than we do. These competitors also compete with us in recruiting and
retaining qualified scientific, sales, marketing and management personnel, establishing clinical trial sites and patient
registration for clinical trials, as well as in acquiring technologies complementary to, or necessary for, our programs.
Smaller or early-stage companies may also prove to be significant competitors, particularly through collaborative
arrangements with large and established companies.

There are currently no therapies approved to treat Galactosemia. Two companies have announced plans for
preclinical or conceptual programs to develop gene therapies in Galactosemia. We believe these potential AAV gene
therapies are several years away from entering the clinic, and there is no data to date in preclinical or clinical studies
demonstrating efficacy or safety. Additionally, due to safety issues associated with AAV gene therapy in general, and the
fact that Galactosemia is a debilitating but not life-threatening disease, we do not believe that the risk appetite of parents or
physicians will support substantial competition from gene therapies.

There are currently no therapies approved for SORD Deficiency. There are no drugs in development to our
knowledge outside of AT-007, and we believe that the IP licensed from University of Miami is sufficiently broad to
encompass the entire class of aldose reductase inhibitors for treatment of SORD Deficiency.

There are currently no therapies approved to treat DbCM. Sponsors of sodium-glucose cotransporter-2, or SGLT2,

inhibitors are pursuing broad cardiovascular labels in type 2 diabetes patients, which may include a subset of DbCM
patients as part of the larger diabetic population at risk for heart failure. Many of these programs are sponsored by large
pharmaceutical companies with a strong presence in cardiology and metabolic disease. There have been prior studies
demonstrating effectiveness in DbCM of off-label use of sildenafil, although we do not believe this represents a
commercially viable competitive threat.

There are no disease modifying therapies approved to treat DPN outside of Japan, India and China. In these

limited markets, epalrestat, another ARI, is approved to prevent worsening of DPN, and despite challenges in compliance
due to frequent dosing three to five times daily, the drugs are generic and offer a low cost alternative. A more effective
therapy with improved tolerability and dosing may offer an advantage. A re-formulation of proprietary crystalline
epalrestat, BNV-222, is in development for DPN in Russia in a 12-month Phase 2/3 clinical trial, which completed
enrollment in 2016, but has not yet reported any results.

There are several therapies approved to treat severe or late-stage forms of DR, or proliferative DR, such as
diabetic macular edema and proliferative DR, including anti-VEGF therapies, Lucentis and Eylea, which represents
approximately 20% of the larger DR population. There are currently no therapies approved to treat non-proliferative DR,
an earlier stage of the disease upstream of vessel or capillary proliferation. However, there are significant additional
clinical development efforts for other mechanistic interventions in early-stage or for non-proliferative DR.

Intellectual Property

Our intellectual property is critical to our business and we strive to protect it, including by obtaining and
maintaining patent protection in the United States and internationally for our product candidates, new therapeutic
approaches and potential indications, and other inventions that are important to our business. Our policy is to seek to
protect our proprietary and intellectual property position by, among other methods, filing U.S. and foreign patent
applications related to our proprietary technology, inventions and improvements that are important for the development and
implementation of our business. We also rely on the skills, knowledge and experience of our scientific and technical
personnel, as well as that of our advisors, consultants and other contractors. To help protect our proprietary know-how that
is not patentable, we rely on confidentiality agreements to protect our interests. We require our employees, consultants and
advisors to enter into confidentiality agreements prohibiting the disclosure of confidential information

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and requiring disclosure and assignment to us of the ideas, developments, discoveries and inventions important to our
business.

Our patent portfolio includes patents and patent applications that are exclusively licensed from Columbia
University and patent applications that are owned by us. Our patent portfolio includes patents and patent applications that
cover our product candidates AT-007, AT-001, and AT-003, and the use of these candidates for therapeutic purposes in
certain territories. Our proprietary technology has been developed primarily through relationships with academic research
centers and contract research organizations.

For our product candidates, we will, in general, initially pursue patent protection covering compositions of matter

and methods of use. Throughout the development of our product candidates, we seek to identify additional means of
obtaining patent protection that would potentially enhance commercial success, including through additional methods of
use, process of making, formulation and dosing regimen-related claims.

In total, our patent portfolio, including patents licensed from Columbia University and patents owned by us,

comprises nine different patent families, filed in various jurisdictions worldwide, including families directed to
composition of matter for AR inhibitors, and families directed to methods of treating Galactosemia and complications
associated with Galactosemia, SORD Deficiency and PMM2-CDG using AR inhibitors. Our patent portfolio includes
issued patents in the United States, Europe, Japan, Australia, Canada, and other jurisdictions. Our patent portfolio is
outlined below:

Composition of Matter Patents

AT-007. We have exclusively licensed a patent family from Columbia University that includes two issued 
composition of matter patents and two issued method use of patents in the United States, and 40 issued patents in Europe, 
Japan, Australia, India, Israel, China, Mexico and South Africa, that claim the composition of matter of and certain 
methods of use with respect to AT 007.  In addition, we have pending patent applications in the United States, Europe, 
Japan, China, Canada, Australia, Russia, Brazil, India, Israel, Mexico, New Zealand, Singapore, South Africa, and Hong 
Kong. The 20-year term of patents in this family runs through June 2037, absent any available patent term adjustments or 
extensions.

AT-001 and AT-003. We have exclusively licensed from Columbia University a patent family that includes five

issued patents in the United States, 82 issued patents in Europe, Japan, Canada, and Australia, a pending application in the
United States and a pending application in Europe that claim the composition of matter of and certain methods of use with
respect to AT-001 and AT-003. The 20-year term of the patents in this family runs through July 2031, absent any available
patent term adjustments or extensions.

Methods for Treating Galactosemia

We own a family of patent applications that claims methods for treating Galactosemia and preventing

complications associated with Galactosemia using AT-007 and other inhibitors of AR. This family currently includes
granted patents in the United States and Mexico, and pending patent application in the United States, Europe, Japan,
Australia, Brazil, Canada, China, Israel, Mexico, New Zealand, Russia, Singapore, South Africa, and Hong Kong. The 20-
year term of patents in this family run through July 2038, absent any available patent term adjustments or extensions.

Methods for Treating SORD Deficiencies

We own a family of patent applications that claims methods for treating SORD Deficiency using AT-007 and other
inhibitors of AR. This family currently includes pending patent applications in the United States, Europe, Japan, Australia,
Brazil, Canada, China, Israel, Mexico, New Zealand, Russia, Singapore, South Africa and South Korea. No patents have
issued to date, but we expect that the 20-year term of any patents that do issue in this family will run through 2041, absent
any available patent term adjustments or extensions.

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We have exclusively licensed a patent family from University of Miami that includes pending applications in the

United States, Europe, Japan, Australia, Brazil, Canada, China, Israel, Mexico, New Zealand, India, Russia, Singapore,
South Africa, South Korea and Hong Kong, that claims methods for treating inherited neuropathy using a variety of
therapeutic modalities including inhibitors of AR. This patent family is owned by University of Miami, University of
Rochester and UCL Business Ltd. and licensed to us by University of Miami pursuant to an exclusive agency granted to
University of Miami, by University of Rochester and UCL Business Ltd. No patents have issued to date, but we expect that
the 20-year term of any patents that do grant in this family will run through 2040, absent any available patent term
adjustments or extensions.

Methods for Treating PMM2-CDG

We own a family of patent applications that claim methods for treating PMM2-CDG using AT-007 and other

inhibitors of AR. This family currently includes pending patent application in the United States, Europe, Japan, Australia,
Brazil, Canada, China, Israel, Mexico, New Zealand, Singapore, South Africa and Hong Kong. No patents have issued to
date, but we expect that the 20-year term of any patents that do grant in this family will run through 2040, absent any
available patent term adjustments or extensions.

We expect to file future patent applications on innovations that are developed in the course of advancing our

pipeline through preclinical and clinical development.

Patent Term and Term Extensions

Individual patents have terms for varying periods depending on the date of filing of the patent application or the
date of patent issuance and the legal term of patents in the countries in which they are obtained. Generally, utility patents
issued for applications filed in the United States are granted a term of 20 years from the earliest effective filing date of a
non-provisional patent application. In addition, in certain instances, the term of a U.S. patent can be extended to recapture a
portion of the United States Patent and Trademark Office, or the USPTO, delay in issuing the patent as well as a portion of
the term effectively lost as a result of the FDA regulatory review period. However, as to the FDA component, the
restoration period cannot be longer than five years and the restoration period cannot extend the patent term beyond
14 years from FDA approval. In addition, only one patent applicable to an approved drug is eligible for the extension, and
only those claims covering the approved drug, a method for using it, or a method of manufacturing may be extended. The
duration of foreign patents varies in accordance with provisions of applicable local law, but typically is also 20 years from
the earliest effective filing date. All taxes, annuities or maintenance fees for a patent, as required by the USPTO and
various foreign jurisdictions, must be timely paid in order for the patent to remain in force during this period of time.

The actual protection afforded by a patent may vary on a product by product basis, from country to country, and

can depend upon many factors, including the type of patent, the scope of its coverage, the availability of regulatory-related
extensions and the availability of legal remedies in a particular country and the validity and enforceability of the patent.

Our patents and patent applications may be subject to procedural or legal challenges by others. We may be unable
to obtain, maintain and protect the intellectual property rights necessary to conduct our business, and we may be subject to
claims that we infringe or otherwise violate the intellectual property rights of others, which could materially harm our
business. For more information, see the section titled “Risk Factors — Risks Related to Our Intellectual Property.”

Trademarks and Know-How

In connection with the ongoing development and advancement of our products and services in the United States

and various international jurisdictions, we seek to create protection for our marks and enhance their value by pursuing
trademarks and service marks where available and when appropriate. In addition to patent and trademark protection, we
rely upon know-how and continuing technological innovation to develop and maintain our competitive position. We

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seek to protect our proprietary information, in part, by using confidentiality agreements with our commercial partners,
collaborators, employees and consultants, and invention assignment agreements with our employees and consultants. These
agreements are designed to protect our proprietary information and, in the case of the invention assignment agreements, to
grant us ownership of technologies that are developed by our employees and through relationships with third parties. These
agreements may be breached, and we may not have adequate remedies for any breach. In addition, our trade secrets may
otherwise become known or be independently discovered by competitors. To the extent that our contractors, commercial
partners, collaborators, employees, and consultants use intellectual property owned by others in their work for us, disputes
may arise as to the rights in related or resulting know-how and inventions. For more information, see the section titled
“Risk Factors — Risks Related to Our Intellectual Property.”

Government Regulation and Product Approval

Government authorities in the United States, at the federal, state and local levels, and in other countries,

extensively regulate, among other things, the research, development, testing, manufacture, pricing, quality control,
packaging, storage, recordkeeping, labeling, advertising, promotion, distribution, marketing, import and export of
pharmaceutical products, such as those we are developing. The processes for obtaining regulatory approvals in the United
States and in foreign countries, along with subsequent compliance with applicable statutes and regulations, require the
expenditure of substantial time and financial resources.

United States Government Regulation

In the United States, the FDA regulates drugs under the Federal Food, Drug, and Cosmetic Act, or FDCA, and its
implementing regulations. The process of obtaining regulatory approvals and the subsequent compliance with appropriate
federal, state, local and foreign statutes and regulations requires the expenditure of substantial time and financial resources.
Failure to comply with the applicable United States requirements at any time during the drug development process,
approval process or after approval, may subject an applicant to delays and a variety of administrative or judicial sanctions,
such as the FDA’s refusal to approve a pending New Drug Application, or NDA, withdrawal of an approval, imposition of
a clinical hold, issuance of warning or untitled letters, product recalls, product seizures, total or partial suspension of
production or distribution, injunctions, fines, refusals of government contracts, restitution, disgorgement or civil or criminal
penalties.

The process required by the FDA before a drug may be marketed in the United States generally involves:

● completion of preclinical laboratory tests, animal studies and formulation studies in compliance with the

FDA’s good laboratory practice, or GLP, regulations;

● submission to the FDA of an IND, which must become effective before human clinical trials may begin;

● approval by an independent institutional review board, or IRB, at each clinical site before each trial may be

initiated;

● performance of adequate and well-controlled clinical trials, in accordance with good clinical practice, or

GCP, requirements to establish the safety and efficacy of the proposed drug for each indication;

● submission to the FDA of an NDA for marketing approval, which must include data from preclinical testing

and clinical trials;

● satisfactory completion of an FDA advisory committee review, if applicable;

● satisfactory completion of an FDA pre-approval inspection of the manufacturing facility or facilities at which
the product is produced to assess compliance with cGMP requirements, and to assure that the facilities,
methods and controls are adequate to preserve the drug’s identity, strength, quality and purity;

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● satisfactory completion of an FDA inspection of selected clinical sites to assure compliance with GCPs and

the integrity of the clinical data;

● payment of user fees; and

● FDA review and approval of the NDA.

Preclinical Studies

Preclinical studies include laboratory evaluation of product chemistry, toxicity and formulation, as well as animal
studies to assess potential safety and efficacy. An IND sponsor must submit the results of the preclinical tests, together with
manufacturing information, analytical data and any available clinical data or literature, among other things, to the FDA as
part of an IND. Some preclinical testing may continue even after the IND is submitted. An IND automatically becomes
effective 30 days after receipt by the FDA, unless before that time the FDA raises concerns or questions related to one or
more proposed clinical trials and places the clinical trial on a clinical hold or a partial clinical hold.

In such a case, the IND sponsor and the FDA must resolve any outstanding concerns before the clinical trial can

begin. As a result, submission of an IND may not result in the FDA allowing clinical trials to commence.

Clinical Trials

Clinical trials involve the administration of the investigational new drug to human subjects under the supervision of
qualified investigators in accordance with GCP requirements, which include the requirement that all research subjects
provide their informed consent in writing for their participation in any clinical trial. Clinical trials are conducted under
protocols detailing, among other things, the objectives of the trial, the parameters to be used in monitoring safety and the
effectiveness criteria to be evaluated. A protocol for each clinical trial and any subsequent protocol amendments must be
submitted to the FDA as part of the IND. In addition, an IRB at each institution participating in the clinical trial must
review and approve the plan for any clinical trial before it commences at that institution, and the IRB must continue to
oversee the clinical trial while it is being conducted and reapprove the study at least annually. Information about certain
clinical trials must be submitted within specific timeframes to the National Institutes of Health, or NIH, for public
dissemination on their ClinicalTrials.gov website. The Food and Drug Omnibus Reform Act, or FDORA, which was
signed into law on December 29, 2022, made numerous amendments to the FDCA including provisions intended to, among
other things, decentralize and modernize clinical trials and enhance diversity in clinical trial populations.

Human clinical trials are typically conducted in three sequential phases, which may overlap or be combined. In

Phase 1, the drug is initially introduced into healthy human subjects or patients with the target disease or condition and
tested for safety, dosage tolerance, absorption, metabolism, distribution, excretion and, if possible, to gain an initial
indication of its effectiveness. In Phase 2, the drug typically is administered to a limited patient population to identify
possible adverse effects and safety risks, to preliminarily evaluate the efficacy of the product for specific targeted diseases
and to determine dosage tolerance and optimal dosage. In Phase 3, the drug is administered to an expanded patient
population, generally at geographically dispersed clinical trial sites, in well-controlled clinical trials to generate enough
data to statistically evaluate the safety and efficacy of the product for approval, to establish the overall risk-benefit profile
of the product and to provide adequate information for the labeling of the product.

Progress reports detailing the results of the clinical trials must be submitted, at least annually, to the FDA, and

more frequently if serious adverse events occur. Phase 1, Phase 2 and Phase 3 clinical trials may not be completed
successfully within any specified period, or at all. Furthermore, the FDA or the sponsor may suspend or terminate a clinical
trial at any time on various grounds, including a finding that the research subjects are being exposed to an unacceptable
health risk. In addition, IND safety reports must be submitted to the FDA for any of the following: serious and unexpected
suspected adverse reactions, findings from other studies or animal or in vitro testing that suggest a significant risk in
humans exposed to the product, and any clinically important increase in the case of a serious suspected adverse reaction
over that listed in the protocol or investigator brochure. Similarly, an IRB can suspend or terminate

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approval of a clinical trial at its institution if the clinical trial is not being conducted in accordance with the IRB’s
requirements, or if the drug has been associated with unexpected serious harm to patients.

Marketing Approval

Assuming successful completion of the required clinical testing, the results of the preclinical and clinical studies,
together with detailed information relating to the product’s chemistry, manufacture, controls and proposed labeling, among
other things, are submitted to the FDA as part of an NDA requesting approval to market the product for one or more
indications. In most cases, the submission of an NDA is subject to a substantial application user fee. Under the Prescription
Drug User Fee Act, or PDUFA, guidelines that are currently in effect, the FDA has a goal of ten months from the date of
“filing” of a standard NDA for a new molecular entity to review and act on the submission. This review typically takes
12 months from the date the NDA is submitted to the FDA because the FDA has approximately two months to make a
“filing” decision. The FDA may further extend the review process for three additional months to consider new information
provided by the applicant to address any outstanding deficiency identified by the FDA following the original submission.

In addition, under the Pediatric Research Equity Act, certain NDAs or supplements to an NDA must contain data

that are adequate to assess the safety and effectiveness of the drug for the claimed indications in all relevant pediatric
subpopulations, and to support dosing and administration for each pediatric subpopulation for which the product is safe and
effective. The FDA may, on its own initiative or at the request of the applicant, grant deferrals for submission of some or
all pediatric data until after approval of the product for use in adults, or full or partial waivers from the pediatric data
requirements. Unless otherwise required by regulation, the pediatric data requirements do not apply to products with
orphan designation.

The FDA also may require submission of a risk evaluation and mitigation strategy, or REMS, plan to ensure that

the benefits of the drug outweigh its risks. The REMS plan could include medication guides, physician communication
plans, assessment plans, and/or elements to assure safe use, such as restricted distribution methods, patient registries or
other risk minimization tools.

The FDA conducts a preliminary review of all NDAs within the first 60 days after submission, before accepting
them for filing, to determine whether they are sufficiently complete to permit substantive review. The FDA may request
additional information rather than accept an NDA for filing. In this event, the application must be resubmitted with the
additional information. The resubmitted application is also subject to review before the FDA accepts it for filing. Once the
submission is accepted for filing, the FDA begins an in-depth substantive review. The FDA reviews an NDA to determine,
among other things, whether the drug is safe and effective and whether the facility in which it is manufactured, processed,
packaged or held meets standards designed to assure the product’s continued safety, quality and purity.

The FDA may refer an application for a novel drug to an advisory committee. An advisory committee is a panel of

independent experts, including clinicians and other scientific experts, that reviews, evaluates and provides a
recommendation as to whether the application should be approved and under what conditions. The FDA is not bound by
the recommendations of an advisory committee, but it considers such recommendations carefully when making decisions.

Before approving an NDA, the FDA typically will inspect the facility or facilities where the product is

manufactured. These pre-approval inspections may cover all facilities associated with an NDA submission, including
component manufacturing, finished product manufacturing and control testing laboratories. The FDA will not approve an
application unless it determines that the manufacturing processes and facilities are in compliance with cGMP requirements
and adequate to assure consistent production of the product within required specifications. Additionally, before approving
an NDA, the FDA will typically inspect one or more clinical trial sites to assure compliance with GCP requirements.

The testing and approval process for an NDA requires substantial time, effort and financial resources, and takes

several years to complete. Data obtained from preclinical and clinical testing are not always conclusive and may be

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susceptible to varying interpretations, which could delay, limit or prevent regulatory approval. The FDA may not grant
approval of an NDA on a timely basis, or at all.

After evaluating the NDA and all related information, including the advisory committee recommendation, if any,
and inspection reports regarding the manufacturing facilities and clinical trial sites, the FDA may issue an approval letter,
or, in some cases, a complete response letter. A complete response letter generally contains a statement of specific
conditions that must be met in order to secure final approval of the NDA and may require additional clinical or preclinical
testing in order for FDA to reconsider the application. Even with submission of this additional information, the FDA
ultimately may decide that the application does not satisfy the regulatory criteria for approval. If and when those conditions
have been met to the FDA’s satisfaction, the FDA will typically issue an approval letter. An approval letter authorizes
commercial marketing of the drug with specific prescribing information for specific indications.

Even if the FDA approves a product, it may limit the approved indications for use of the product, require that

contraindications, warnings or precautions be included in the product labeling, require that post-approval studies, including
Phase 4 clinical trials, be conducted to further assess a drug’s safety after approval, require testing and surveillance
programs to monitor the product after commercialization, or impose other conditions, including distribution and use
restrictions or other risk management mechanisms under a REMS, which can materially affect the potential market and
profitability of the product. The FDA may prevent or limit further marketing of a product based on the results of post-
marketing studies or surveillance programs. After approval, some types of changes to the approved product, such as adding
new indications, manufacturing changes, and additional labeling claims, are subject to further testing requirements and
FDA review and approval.

Orphan Drug Designation

Under the Orphan Drug Act, the FDA may grant orphan drug designation to a drug intended to treat a rare disease
or condition, which is a disease or condition that affects fewer than 200,000 individuals in the United States, or if it affects
more than 200,000, there is no reasonable expectation that sales of the drug in the United States will be sufficient to offset
the costs of developing and making the drug available in the United States. Orphan drug designation must be requested
before submitting an NDA. Orphan drug designation does not convey any advantage in or shorten the duration of the
regulatory review and approval process.

If the FDA approves a sponsor’s marketing application for a designated orphan drug for use in the rare disease or

condition for which it was designated, the sponsor is eligible for a seven-year period of marketing exclusivity, during
which the FDA may not approve another sponsor’s marketing application for a drug with the same active moiety and
intended for the same use or indication as the approved orphan drug, except in limited circumstances, such as if a
subsequent sponsor demonstrates its product is clinically superior. During a sponsor’s orphan drug exclusivity period,
competitors, however, may receive approval for drugs with different active moieties for the same indication as the
approved orphan drug, or for drugs with the same active moiety as the approved orphan drug, but for different indications.
Orphan drug exclusivity could block the approval of one of our product candidates for seven years if a competitor obtains
approval for a drug with the same active moiety intended for the same indication before we do, unless we are able to
demonstrate that grounds for withdrawal of the orphan drug exclusivity exist, such as that our product is clinically superior.
Further, if a designated orphan drug receives marketing approval for an indication broader than the rare disease or
condition for which it received orphan drug designation, it may not be entitled to exclusivity.

Special FDA Expedited Review and Approval Programs

The FDA has various programs, including fast track designation, priority review, accelerated approval and

breakthrough therapy designation, which are intended to expedite or simplify the process for the development and FDA
review of drugs that are intended for the treatment of serious or life-threatening diseases or conditions and demonstrate the
potential to address unmet medical needs. The purpose of these programs is to provide important new drugs to patients
earlier than under standard FDA review procedures.

To be eligible for a fast track designation, the FDA must determine, based on the request of a sponsor, that a

product is intended to treat a serious or life-threatening disease or condition and demonstrates the potential to address an

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unmet medical need. The FDA will determine that a product will fill an unmet medical need if it will provide a therapy
where none exists or provide a therapy that may be potentially superior to existing therapy based on efficacy or safety
factors. The FDA may review sections of the NDA for a fast track product on a rolling basis before the complete
application is submitted. The FDA may do so if the sponsor provides a schedule for the submission of the sections of the
NDA, the FDA agrees to accept sections of the NDA and determines that the schedule is acceptable, and the sponsor pays
any required user fees upon submission of the first section of the NDA.

The FDA may give a priority review designation to drugs that are designed to treat serious conditions, and if

approved, would provide a significant improvement in treatment, or provide a treatment where no adequate therapy exists.
A priority review means that the goal for the FDA to review an application is six months, rather than the standard review of
ten months under current PDUFA guidelines. Under the current PDUFA agreement, these six and ten-month review periods
are measured from the “filing” date rather than the receipt date for NDAs for new molecular entities, which typically adds
approximately two months to the timeline for review and decision from the date of submission. Most products that are
eligible for fast track designation are also likely to be considered appropriate to receive a priority review.

Rare pediatric disease, or RPD, designation by the FDA enables priority review voucher, or PRV, eligibility upon

U.S. market approval of a designated drug for rare pediatric diseases. The RPD-PRV program is intended to encourage
development of therapies to prevent and treat rare pediatric diseases. The voucher, which is awarded upon NDA or
Biologics License Application, or BLA, approval to the sponsor of a designated RPD can be sold or transferred to another
entity and used by the holder to receive priority review for a future NDA or BLA submission, which reduces the FDA
review time of such future submission from ten to six months. The RPD-PRV program is currently scheduled to sunset as
of September 30, 2026.

In addition, products studied for their safety and effectiveness in treating serious or life-threatening illnesses and that
provide meaningful therapeutic benefit over existing treatments may be eligible for accelerated approval. To qualify, the
FDA must determine that the drug product has an effect on a surrogate endpoint that is reasonably likely to predict clinical
benefit, or on a clinical endpoint that can be measured earlier than irreversible morbidity or mortality, that is reasonably
likely to predict an effect on irreversible morbidity or mortality or other clinical benefit, taking into account the severity,
rarity or prevalence of the condition and the availability or lack of alternative treatments. As a condition of approval, the
FDA may require a sponsor of a drug receiving accelerated approval to perform post-marketing studies to verify and
describe the predicted effect on irreversible morbidity or mortality or other clinical endpoint, and the drug may be subject
to accelerated withdrawal procedures. Among FDORA’s provisions are amendments to the accelerated approval program,
including new requirements relating to post-approval studies and enhanced enforcement and withdrawal authorities for the
FDA.

Breakthrough therapy designation is for a drug that is intended, alone or in combination with one or more other
drugs, to treat a serious or life-threatening disease or condition, and preliminary clinical evidence indicates that the drug
may demonstrate substantial improvement over existing therapies on one or more clinically significant endpoints, such as
substantial treatment effects observed early in clinical development. The FDA must take certain actions, such as holding
timely meetings and providing advice, intended to expedite the development and review of an application for approval of a
breakthrough therapy.

Even if a product qualifies for one or more of these programs, the FDA may later decide that the product no

longer meets the conditions for qualification or decide that the time period for FDA review or approval will not be
shortened. We may explore some of these opportunities for our product candidates as appropriate.

Post-Approval Requirements

Drugs manufactured or distributed pursuant to FDA approvals are subject to pervasive and continuing regulation
by the FDA, including, among other things, requirements relating to recordkeeping, periodic reporting, product sampling
and distribution, advertising and promotion and reporting of adverse experiences with the product. After approval, most
changes to the approved product, such as adding new indications, manufacturing changes or other labeling claims, are
subject to further testing requirements and prior FDA review and approval. There also are continuing

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annual user fee requirements for any marketed products and the establishments at which such products are manufactured,
as well as application fees for supplemental applications with clinical data.

Even if the FDA approves a product, it may limit the approved indications for use of the product, require that
contraindications, warnings or precautions be included in the product labeling, including a boxed warning, require that
post-approval studies, including Phase 4 clinical trials, be conducted to further assess a drug’s safety after approval, require
testing and surveillance programs to monitor the product after commercialization, or impose other conditions, including
distribution restrictions or other risk management mechanisms under a REMS, which can materially affect the potential
market and profitability of the product. The FDA may prevent or limit further marketing of a product based on the results
of post-marketing studies or surveillance programs.

In addition, drug manufacturers and other entities involved in the manufacture and distribution of approved drugs

are required to register their establishments with the FDA and state agencies, and are subject to periodic unannounced
inspections by the FDA and these state agencies for compliance with cGMP requirements.

Changes to the manufacturing process are strictly regulated and often require prior FDA approval before being

implemented. FDA regulations also require investigation and correction of any deviations from cGMP and impose
reporting and documentation requirements upon the sponsor and any third party manufacturers that the sponsor may decide
to use. Accordingly, manufacturers must continue to expend time, money and effort in the area of production and quality
control to maintain compliance with cGMP and other regulatory requirements.

The FDA may also subject a drug to official lot release, which requires manufacturers to submit several items to
the FDA with respect to each lot of a drug before it is released to distribution. These items include samples of each lot, a
summary of the manufacturing history of the lot and the results of any tests performed on the lot.

Once an approval is granted, the FDA may withdraw the approval if compliance with regulatory requirements and

standards is not maintained or if problems occur after the product reaches the market.

Later discovery of previously unknown problems with a product, including adverse events of unanticipated

severity or frequency, problems with manufacturing processes, or failure to comply with regulatory requirements, may
result in mandatory revisions to the approved labeling to add new safety information; imposition of post-market studies or
clinical trials to assess new safety risks; or imposition of distribution or other restrictions under a REMS program. Other
potential consequences include, among other things:

● restrictions on the marketing or manufacturing of the product, complete withdrawal of the product from the

market or product recalls;

● fines, warning letters or holds on post-approval clinical trials;

● refusal of the FDA to approve pending NDAs or supplements to approved NDAs, or suspension or

revocation of product approvals;

● product seizure or detention, or refusal to permit the import or export of products; or

● injunctions or the imposition of civil or criminal penalties.

The FDA strictly regulates marketing, labeling, advertising and promotion of products that are placed on the

market. Drugs may be promoted only for the approved indications and in accordance with the provisions of the approved
label, although physicians, in the practice of medicine, may prescribe approved drugs for unapproved indications. The FDA
and other agencies actively enforce the laws and regulations prohibiting their promotion of off-label uses, and a company
that is found to have improperly promoted off-label uses may be subject to significant civil, criminal and administrative
liability.

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In addition, the distribution of prescription pharmaceutical products is subject to the Prescription Drug Marketing
Act, or PDMA, which regulates the distribution of drugs and drug samples at the federal level, and sets minimum standards
for the registration and regulation of drug distributors by the states. Both the PDMA and state laws limit the distribution of
prescription pharmaceutical product samples and impose requirements to ensure accountability in distribution.

Federal and State Fraud and Abuse, Data Privacy and Security, and Transparency Laws and Regulations

In addition to FDA restrictions on marketing of pharmaceutical products, federal and state healthcare laws and

regulations restrict business practices in the biopharmaceutical industry. These laws may impact, among other things, our
current and future business operations, including our clinical research activities and proposed sales, marketing and
education programs and constrain the business or financial arrangements and relationships with healthcare providers and
other parties through which we may market, sell and distribute any products for which we obtain marketing approval.
These laws include anti-kickback and false claims laws and regulations, data privacy and security, and transparency laws
and regulations, including, without limitation, those laws described below.

The federal Anti-Kickback Statute prohibits any person or entity from, among other things, knowingly and

willfully offering, paying, soliciting or receiving remuneration to induce or in return for purchasing, leasing, ordering or
arranging for or recommending the purchase, lease or order of any item or service reimbursable under Medicare, Medicaid
or other federal healthcare programs. The term “remuneration” has been broadly interpreted to include anything of value.
The federal Anti-Kickback Statute has been interpreted to apply to arrangements between pharmaceutical manufacturers on
the one hand and prescribers, purchasers and formulary managers on the other. Although there are a number of statutory
exceptions and regulatory safe harbors protecting some common activities from prosecution, the exceptions and safe
harbors are drawn narrowly. Practices that involve remuneration that may be alleged to be intended to induce prescribing,
purchases or recommendations may be subject to scrutiny if they do not qualify for an exception or safe harbor. Several
courts have interpreted the statute’s intent requirement to mean that if any one purpose of an arrangement involving
remuneration is to induce referrals of federal healthcare covered business, the statute has been violated.

A person or entity does not need to have actual knowledge of this statute or specific intent to violate it in order to
have committed a violation. In addition, the government may assert that a claim including items or services resulting from
a violation of the federal Anti-Kickback Statute constitutes a false or fraudulent claim for purposes of the federal civil
False Claims Act or the civil monetary penalties laws.

Federal civil and criminal false claims laws and civil monetary penalties laws, including the federal civil False

Claims Act, which can be enforced by individuals through civil whistleblower or qui tam actions, prohibits any person or
entity from, among other things, knowingly presenting, or causing to be presented, a false claim for payment to the federal
government or knowingly making, using or causing to be made or used a false record or statement material to a false or
fraudulent claim to the federal government. A claim includes “any request or demand” for money or property presented to
the U.S. government. Several pharmaceutical and other healthcare companies have been prosecuted under these laws for
allegedly providing free product to customers with the expectation that the customers would bill federal programs for the
product. Other companies have been prosecuted for causing false claims to be submitted because of the companies’
marketing of products for unapproved, and thus non-reimbursable, uses.

The federal Health Insurance Portability and Accountability Act of 1996, or HIPAA, created additional federal

criminal statutes that prohibit, among other things, knowingly and willfully executing a scheme to defraud any healthcare
benefit program, including private third party payors and knowingly and willfully falsifying, concealing or covering up a
material fact or making any materially false, fictitious or fraudulent statement in connection with the delivery of or
payment for healthcare benefits, items or services. Also, many states have similar fraud and abuse statutes or regulations
that apply to items and services reimbursed under Medicaid and other state programs, or, in several states, apply regardless
of the payor.

In addition, we may be subject to data privacy and security regulation by both the federal government and the
states in which we conduct our business. HIPAA, as amended by the Health Information Technology for Economic and

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Clinical Health Act, or HITECH, and their respective implementing regulations, impose specified requirements on certain
types of individuals and entities relating to the privacy, security and transmission of individually identifiable health
information. Among other things, HITECH makes HIPAA’s security standards directly applicable to “business associates,”
defined as independent contractors or agents of covered entities, which include certain healthcare providers, healthcare
clearinghouses and health plans, that create, receive, maintain or transmit individually identifiable health information in
connection with providing a service for or on behalf of a covered entity. HITECH also increased the civil and criminal
penalties that may be imposed against covered entities, business associates and possibly other persons, and gave state
attorneys general new authority to file civil actions for damages or injunctions in federal courts to enforce HIPAA and seek
attorney’s fees and costs associated with pursuing federal civil actions. In addition, state laws govern the privacy and
security of health information in certain circumstances, many of which are not pre-empted by HIPAA, differ from each
other in significant ways and may not have the same effect, thus complicating compliance efforts.

The federal Physician Payments Sunshine Act requires certain manufacturers of drugs, devices, biologics and

medical supplies for which payment is available under Medicare, Medicaid or the Children’s Health Insurance Program,
with specific exceptions, to report annually to the Centers for Medicare & Medicaid Services, or CMS, information related
to payments or other transfers of value made to physicians and teaching hospitals, and applicable manufacturers and
applicable group purchasing organizations to report annually to CMS ownership and investment interests held by
physicians and their immediate family members.

We may also be subject to state laws that require pharmaceutical companies to comply with the pharmaceutical

industry’s voluntary compliance guidelines and the relevant compliance guidance promulgated by the federal government,
state laws that require drug manufacturers to report information related to payments and other transfers of value to
physicians and other healthcare providers or marketing expenditures, and state and local laws that require the registration
of pharmaceutical sales representatives. State legislatures are increasingly focused on pharmaceutical company activities,
and we may be subject to additional new state or federal legislative requirements in the future that could impact our ability
to commercialize our product candidates, if they are approved.

Because of the breadth of these laws and the narrowness of available statutory exceptions and regulatory safe

harbors, it is possible that some of our business activities could be subject to challenge under one or more of such laws. If
our operations are found to be in violation of any of the federal and state laws described above or any other governmental
regulations that apply to us, we may be subject to significant criminal, civil and administrative penalties including
damages, fines, individual imprisonment, additional reporting requirements and oversight if we become subject to a
corporate integrity agreement or similar agreement to resolve allegations of non-compliance with these laws, contractual
damages, reputational harm, diminished profits and future earnings, disgorgement, exclusion from participation in
government healthcare programs and the curtailment or restructuring of our operations, any of which could adversely affect
our ability to operate our business and our results of operations. To the extent that any of our product candidates are sold in
a foreign country, we may be subject to similar foreign laws and regulations, which may include, for instance, applicable
post-marketing requirements, including safety surveillance, anti-fraud and abuse laws, implementation of corporate
compliance programs, reporting of payments or transfers of value to healthcare professionals, and additional data privacy
and security requirements.

Coverage and Reimbursement

The future commercial success of our product candidates, if approved, will depend in part on the extent to which
third party payors, such as governmental payor programs at the federal and state levels, including Medicare and Medicaid,
private health insurers and other third party payors, provide coverage of and establish adequate reimbursement levels for
our product candidates. Third party payors generally decide which products they will pay for and establish reimbursement
levels for those products. In particular, in the United States, no uniform policy for coverage and reimbursement exists.
Private health insurers and other third party payors often provide coverage and reimbursement for products based on the
level at which the government, through the Medicare program, provides coverage and reimbursement for such products,
but also on their own methods and approval process apart from Medicare determinations. Therefore, coverage and
reimbursement can differ significantly from payor to payor.

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In the United States, the European Union, or EU, and other potentially significant markets for our product

candidates, government authorities and third party payors are increasingly attempting to limit or regulate the price of
products, particularly for new and innovative products, which often has resulted in average selling prices lower than they
would otherwise be. Further, the increased emphasis on managed healthcare in the United States and on country and
regional pricing and reimbursement controls in the EU will put additional pressure on product pricing, reimbursement and
usage. These pressures can arise from rules and practices of managed care groups, judicial decisions and laws and
regulations related to Medicare, Medicaid and healthcare reform, pharmaceutical coverage and reimbursement policies and
pricing in general.

Third party payors are increasingly imposing additional requirements and restrictions on coverage and limiting

reimbursement levels for products. For example, federal and state governments reimburse products at varying rates
generally below average wholesale price. These restrictions and limitations influence the purchase of products. Third party
payors may limit coverage to specific products on an approved list, or formulary, which might not include all of the FDA-
approved products for a particular indication. Third party payors are increasingly challenging the price and examining the
medical necessity and cost-effectiveness of products, in addition to their safety and efficacy. We may need to conduct
expensive pharmacoeconomic studies in order to demonstrate the medical necessity and cost-effectiveness of our product
candidates, in addition to the costs required to obtain the FDA approvals. Our product candidates may not be considered
medically necessary or cost-effective. A payor’s decision to provide coverage for a product does not imply that an adequate
reimbursement rate will be approved. Adequate third party payor reimbursement may not be available to enable us to
realize an appropriate return on our investment in product development. Legislative proposals to reform healthcare or
reduce costs under government insurance programs may result in lower reimbursement for our product candidates, if
approved, or exclusion of our product candidates from coverage and reimbursement. The cost containment measures that
third party payors and providers are instituting and any healthcare reform could significantly reduce our revenues from the
sale of any approved product candidates.

Healthcare Reform

The United States and some foreign jurisdictions are considering enacting or have enacted a number of additional
legislative and regulatory proposals to change the healthcare system in ways that could affect our ability to sell our product
candidates. The United States and some foreign jurisdictions are considering enacting or have enacted a number of
additional legislative and regulatory proposals to change the healthcare system in ways that could affect our ability to sell
our product candidates profitably, if approved. Among policy makers and payors in the United States and elsewhere, there
is significant interest in promoting changes in healthcare systems with the stated goals of containing healthcare costs,
improving quality and expanding access. In the United States, the pharmaceutical industry has been a particular focus of
these efforts, which include major legislative initiatives to reduce the cost of care through changes in the healthcare system,
including limits on the pricing, coverage, and reimbursement of pharmaceutical and biopharmaceutical products, especially
under government-funded healthcare programs, and increased governmental control of drug pricing.

There have been several U.S. government initiatives over the past few years to fund and incentivize certain

comparative effectiveness research, including creation of the Patient-Centered Outcomes Research Institute under the
Patient Protection and Affordable Care Act of 2010, as amended by the Health Care and Education Reconciliation Act of
2010, or collectively the PPACA. It is also possible that comparative effectiveness research demonstrating benefits in a
competitor’s product could adversely affect the sales of our product candidates.

The PPACA became law in March 2010 and substantially changed the way healthcare is financed by third party

payors, and significantly impacts the U.S. pharmaceutical industry. Among other measures that may have an impact on our
business, the PPACA establishes an annual, nondeductible fee on any entity that manufactures or imports specified branded
prescription drugs and biologic agents; a new Medicare Part D coverage gap discount program; and a new formula that
increases the rebates a manufacturer must pay under the Medicaid Drug Rebate Program. Additionally, the PPACA extends
manufacturers’ Medicaid rebate liability, expands eligibility criteria for Medicaid programs, and expands entities eligible
for discounts under the Public Health Service Act.

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In addition to these provisions, the Affordable Care Act established a number of bodies whose work may have a
future impact on the market for certain pharmaceutical products. These include the Patient-Centered Outcomes Research
Institute, established to oversee, identify priorities in, and conduct comparative clinical effectiveness research and the
Center for Medicare and Medicaid Innovation within the Centers for Medicare and Medicaid Services, to test innovative
payment and service delivery models to lower Medicare and Medicaid spending. At this time, we are unsure of the full
impact that the PPACA will have on our business.

Since its enactment, there have been judicial and Congressional challenges to certain aspects of the PPACA and

we expect such challenges and amendments to continue. Former President Trump implemented certain directives designed
to delay the implementation of certain PPACA provisions or otherwise circumvent requirements for health insurance
mandated by the PPACA, while Congress has considered legislation that would repeal or repeal and replace all or part of
the PPACA. While Congress has not passed comprehensive repeal legislation, bills affecting the implementation of the
PPACA have been signed into law. For example, the Tax Act includes a provision that repealed, effective January 1, 2019,
the tax-based shared responsibility payment imposed by the PPACA on certain individuals who fail to maintain qualifying
health coverage for all or part of a year that is commonly referred to as the “individual mandate.” On December 19, 2020,
former President Trump signed a bill that repealed the PPACA’s so-called “Cadillac” tax on certain high cost employer-
sponsored insurance plans. The Bipartisan Budget Act of 2018, or the BBA, among other things, amended the PPACA,
effective January 1, 2019, to increase from 50% to 70% the point-of-sale discount that is owed by pharmaceutical
manufacturers who participate in Medicare Part D and to close the coverage gap in most Medicare drug plans, commonly
referred to as the “donut hole.” In December 2018, a U.S. District Court Judge in the Northern District of Texas, or Texas
District Court Judge, ruled that the individual mandate is a critical and inseverable feature of the PPACA, and therefore,
because it was repealed as part of the Tax Act, the remaining provisions of the PPACA are invalid as well. In December
2019, the U.S. Court of Appeals for the Fifth Circuit upheld the lower court decision, which was then appealed to the U.S.
Supreme Court. In June 2021, the U.S. Supreme Court held that state and individual plaintiffs did not have standing to
challenge the individual mandate provision of the PPACA; in so holding, the Supreme Court did not consider larger
constitutional questions about the validity of this provision or the validity of the PPACA in its entirety. Another case
challenging the PPACA’s requirement that private insurers cover certain preventative services is currently pending before
the same U.S. District Court Judge in the Northern District of Texas who ruled against the individual mandate in 2018. In
September 2022, the judge held that certain preventative services violated the U.S. Constitution and set a schedule for
additional briefing regarding the scope of the remedy. That briefing was completed in January 2023 and it is unclear when
or how the court will rule. It is also unclear how this or any potential future litigation and other efforts to repeal and replace
the PPACA will impact the PPACA, or our business.

Further, there has been increasing legislative, executive branch, and enforcement interest in the United States with

respect to drug pricing practices. Specifically, there have been several recent U.S. Congressional inquiries and proposed
and enacted federal and state legislation designed to, among other things, bring more transparency to drug pricing, review
the relationship between pricing and manufacturer patient programs, and reform government program reimbursement
methodologies for drugs. With respect to executive branch actions, the former Trump administration released a “Blueprint”
to lower drug prices and reduce out of pocket costs of drugs that contained proposals to increase manufacturer competition,
increase the negotiating power of certain federal healthcare programs, incentivize manufacturers to lower the list price of
their products and reduce the out of pocket costs of drug products paid by consumers. The HHS has implemented some of
these measures under its existing authority. For example, in May 2019, CMS issued a final rule to allow Medicare
Advantage Plans the option of using step therapy for Part B drugs, beginning January 1, 2020. Although a number of these
and other proposed measures will require authorization through additional legislation to become effective, Congress and
the Biden administration have each indicated that it will continue to seek new legislative and/or administrative measures to
control drug costs. For example, the Inflation Reduction Act of 2022, enacted on August 16, 2022, seeks to reduce
prescription drug costs by, among other provisions, allowing Medicare to negotiate prices for certain high-cost prescription
drugs in Medicare Parts B and D, imposing an excise tax on pharmaceutical manufacturers that refuse to negotiate pricing
with Medicare, requiring inflation rebates to limit annual drug price increases in Medicare, redesigning the Medicare Part
D formula, and limiting the cost-sharing for insulin products. It is unclear whether additional drug pricing and other
healthcare reform measures will be enacted, and if enacted, what effect they would have on our business.

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At the state level, legislatures have increasingly passed legislation and implemented regulations designed to

control pharmaceutical and biological product pricing, including price or patient reimbursement constraints, discounts,
restrictions on certain product access and marketing cost disclosure and transparency measures, and, in some cases,
designed to encourage importation from other countries and bulk purchasing. In addition, regional healthcare authorities
and individual hospitals are increasingly using bidding procedures to determine which drugs and suppliers will be included
in their healthcare programs. These measures could reduce future demand for our products or put pressure on our pricing.

Additionally, in May 2018, the Trickett Wendler, Frank Mongiello, Jordan McLinn, and Matthew Bellina Right to

Try Act of 2017, or the Right to Try Act, was signed into law. The law, among other things, provides a federal framework
for certain patients to access certain investigational new drug products that have completed a Phase I clinical trial and that
are undergoing investigation for FDA approval. Under certain circumstances, eligible patients can seek treatment without
enrolling in clinical trials and without obtaining FDA permission under the FDA expanded access program. There is no
obligation for a drug manufacturer to make its drug products available to eligible patients as a result of the Right to Try
Act.

Foreign Regulation

In order to market any product outside of the United States, we would need to comply with numerous and varying
regulatory requirements of other countries regarding safety and efficacy and governing, among other things, clinical trials,
marketing authorization, commercial sales and distribution of our product candidates. For example, in the EU, we must
obtain authorization of a clinical trial application, or CTA, in each member state in which we intend to conduct a clinical
trial. Whether or not we obtain FDA approval for a drug, we would need to obtain the necessary approvals by the
comparable regulatory authorities of foreign countries before we can commence clinical trials or marketing of the drug in
those countries. The approval process varies from country to country and can involve additional product testing and
additional administrative review periods. The time required to obtain approval in other countries might differ from and be
longer than that required to obtain FDA approval. Regulatory approval in one country does not ensure regulatory approval
in another, but a failure or delay in obtaining regulatory approval in one country may negatively impact the regulatory
process in others.

Facilities

We are currently in a five-year lease for the space for our principal executive offices in New York, New York and

a three-year lease for the offices in Englewood Cliffs, New Jersey. We believe that our facilities are adequate to meet our
current needs.

Employees and Human Capital Resources

Investing in, developing, and maintaining human capital is critical to our success. As of December 31, 2022, we 

had 27 full-time employees, 18 of whom were primarily engaged in research and development activities.  A total of ten 
employees have an M.D. or Ph.D. degree. We emphasize a number of measures and objectives in managing our human 
capital assets, including, among others, employee safety and wellness, talent acquisition and retention, employee 
engagement, development and training, diversity and inclusion and compensation and pay equity. None of our employees 
are represented by a labor union and we consider our employee relations to be good.

Our human capital resource objectives include, as applicable, identifying, recruiting, retaining, incentivizing and

integrating our existing and new employees and advisors. The principal purposes of our equity and cash incentive plans are
to attract, retain and reward personnel and increase our success and stockholder value thereby.

The success of our business is fundamentally connected to the well-being of our employees. Accordingly, we are

committed to their health, safety and wellness.

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Information About Our Executive Officers

The following table sets forth information regarding our executive officers:

Name
Executive Officers
Shoshana Shendelman, Ph.D.

Riccardo Perfetti, M.D., Ph.D.

Adam Hansard

Age

44

63

47

Position(s)

President, Chief Executive Officer and Chair of the Board
of Directors

Chief Medical Officer

  Chief Commercial Officer

Shoshana Shendelman, Ph.D., age 44, is our founder and has served as our President and Chief Executive

Officer and as chair of our board of directors since January 2016. Prior to founding our company, she founded Clearpoint
Strategy Group LLC, a boutique life sciences consulting firm, where she served as the Managing Director from July 2012
to December 2016, and served as a Senior Advisor from January 2017 to December 2018. Prior to that, she served as a
scientific consultant and analyst at Bridge Scientific Consulting LLC. Dr. Shendelman received her B.S. in biochemistry
from Brandeis University and a Ph.D. in Cellular, Molecular and Biophysical Studies (CMBS) from Columbia University
Vagelos College of Physicians and Surgeons. We believe that Dr. Shendelman’s extensive knowledge of our company as
founder, President and Chief Executive Officer and her management background and experience in the healthcare industry
qualifies her to serve on our board of directors.

Riccardo Perfetti, M.D., Ph.D., age 63, has served as our Chief Medical Officer since August 2018. Prior to

joining us, Dr. Perfetti served as a Senior Medical Officer, Vice President and Head of Global Medical Affairs, Diabetes
and Cardiovascular Business Unit at Sanofi S.A., a publicly traded pharmaceutical company from October 2007 to
September 2018. Prior to joining Sanofi, Dr. Perfetti served in various roles at Amgen Inc., a publicly traded
biopharmaceutical company, including as a Director and Global Development Leader in diabetes, obesity, metabolism and
endocrinology from December 2004 to August 2007. Dr. Perfetti was previously an associate professor of medicine at
University of California in Los Angeles and a professor of medicine at the National Institutes of Health, or NIH. Dr.
Perfetti practiced as an endocrinologist at Cedars-Sinai Medical Center and also served as Director of the Diabetes
Research Laboratory and Director of the Outpatient Diabetes Program. Dr. Perfetti received his M.D. and Ph.D. in
Endocrinology from University La Sapienza in Rome, Italy and received post-graduate training in endocrinology and
molecular biology at NIH.

Adam Hansard, age 47, has served as our Chief Commercial Officer since March 2020. Prior to joining us, he

was Senior Director of New Product Strategy at Alexion Pharmaceuticals, a biopharmaceutical company, from March 2019
to February 2020. From February 2018 to March 2019, he was Vice President of Business Operations at Syntimmune, a
clinical-stage biotech purchased by Alexion in November 2018. From January 2012 to March 2018, Mr. Hansard worked at
Sanofi Genzyme, a biotechnology company and wholly-owned subsidiary of Sanofi, a publicly traded, multinational
pharmaceutical company, where he served as the North American Senior Director, Chief of Staff of MS Oncology and
Immunology and the Senior Director of MS Brand Communications. Mr. Hansard received his Master’s in Business
Communication from Jones International University and his B.S. in Marketing from the University of West Florida.

Other Information

We were incorporated in Delaware in January 2016 and completed the IPO in May 2019. Our principal executive

offices are located at 545 5th Avenue, Suite 1400, New York, New York 10017, and our telephone number is (212) 220-
9226.

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We maintain a website at www.appliedtherapeutics.com. The contents of our website are not incorporated in, or

otherwise to be regarded as part of this Annual Report. Unless the context otherwise requires, the terms, “Applied
Therapeutics,” the “Company,” “we,” “us,” “our” and the “ registrant” refer to Applied Therapeutics, Inc.

Investors and others should note that we announce material financial information to our investors using our
investor relations website (http://ir.appliedtherapeutics.com), SEC filings, press releases, public conference calls and
webcasts.

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ITEM 1A.      RISK FACTORS.

An investment in shares of our common stock involves a high degree of risk. You should carefully consider the

following information about these risks described below, together with other information appearing elsewhere in this
Annual Report, including our financial statements and the related notes and the section titled “Management’s Discussion
and Analysis of Financial Condition and Results of Operations,” before deciding whether to invest in our common stock.
The occurrence of any of the events or developments described below could harm our business, financial condition, results
of operations and growth prospects. In such an event, the market price of our common stock could decline and you may
lose all or part of your investment.

Additional risks and uncertainties not presently known to us or that we currently deem immaterial also may

impair our business operations and the market price of our common stock.

Risk Factor Summary

The following is a summary of the risk factors included in this Item 1A and is qualified entirely by the disclosure

included in the rest of this Item 1A:

Risks Related to Our Financial Position and Capital Needs

● We have incurred and expect to continue to incur substantial operating losses and our ability to use our net

operating losses to offset future taxable income may be subject to certain limitations.
● Our operating history makes evaluating our business and future viability more difficult.
● We will require substantial additional funding to finance our operations, and may suffer consequences to our

development programs upon failure to do so.

● Raising additional capital may cause adverse effects.

Risks Related to the Development and Commercialization of Our Product Candidates

● Our success is substantially dependent on the successful clinical development, regulatory approval and
commercialization of our product candidates and may be adversely affected upon failure to do so.

● We or Advanz Pharma may fail to perform under any of the agreements entered into in connection with the

partnership for the commercialization of AT-007, which may subject us to liabilities, and we may fail to achieve
anticipated benefits of the partnership.

● Success in preclinical studies or earlier clinical trials may not be indicative of results in future clinical trials and

our results may not be sufficient for the necessary regulatory approvals.

● Clinical drug development involves a lengthy and expensive process and the development of additional product

candidates is risky and uncertain.

● We may be unable to obtain/maintain or receive the benefits of regulatory approval, rare pediatric disease
designation/exclusivity, accelerated registration pathways, breakthrough therapy designations or fast track
designations for our product candidates, as applicable.

● Clinical trials are expensive, time consuming and subject to factors outside our control.
● Our product candidates may cause undesirable side effects, affecting regulatory approval, commercial potential or

result in significant negative consequences following any potential marketing approval.

● Interim, “top line” and preliminary data from our clinical trials may be subject to change.
● The market opportunities for our product candidates may be smaller than we believe or approval we obtain may

narrow our patient population.

● We may face substantial competition.
● We may face risks related to strategic collaborations to develop our product candidates
● Our product candidates may fail to achieve market acceptance necessary for commercial success.
● We may face risks related to any potential international operations.
● We may be adversely affected by product liability lawsuits.
● Our insurance policies may be inadequate and potentially expose us to unrecoverable risks.

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Risks Related to Regulatory Compliance

● We are subject to healthcare laws and regulations, which carry substantial penalties for noncompliance.
● Coverage and adequate reimbursement may not be available for our product candidates.
● Healthcare reform measures may have a negative impact on our business and results of operations.

Risks Related to Our Dependence on Third Parties

● Third-parties may conduct our preclinical studies and clinical trials in an unsatisfactory manner.
● We intend to rely on third parties to produce supplies of our product candidates.
● We and our third-party affiliates are subject to environmental, health and safety laws and regulations.

Risks Related to Our Intellectual Property

● Breaches of our license agreements may result in the adverse effects to our ability to continue the development

and commercialization of our product candidates.

● Insufficient patent protection could allow our competitors to develop and commercialize products and technology

similar or identical to ours.

● Obtaining and maintaining our patent rights is expensive, complicated and labor intensive and patent terms may

be inadequate to protect our competitive position on our product candidates.
● We may be subject to claims alleging violations of intellectual property rights.
● Changes in patent law could impair our ability to protect our product candidates.
● We may be unable to protect our intellectual property rights.
● Intellectual property rights do not necessarily address all potential threats to our business.

Risks Related to Our Business Operations, Employee Matters and Managing Growth

● We are highly dependent on the services of our current executive officers.
● We may experience difficulties resulting from the expansion of our organization.
● We may be subject to security breaches in our information technology systems.
● Our employees and the third-parties we deal with may engage in misconduct or improper activities.
● Our business may be adversely affected by the coronavirus outbreak.

Risks Related to Ownership of Our Common Stock

● The market price of our common stock is volatile and has fluctuated substantially.
● Concentration of ownership of our common stock among our existing executive officers, directors and principal

stockholders may prevent new investors from influencing significant corporate decisions.
● We do not anticipate paying any cash dividends on our capital stock in the foreseeable future.
● Failure to regain compliance with the continued listing requirements of Nasdaq could result in our common stock
being delisted from Nasdaq and the price and liquidity of our common stock could be negatively impacted.

General Risk Factors

● We may be affected by unfavorable research or reports.
● We may use our cash and cash equivalents ineffectively or in ways with which you do not agree.
● We are subject to risks as an “emerging growth company” and a public company.
● We may avail ourselves of defensive and forum selection provisions in our governing documents and under

Delaware law.

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Risks Related to Our Financial Position and Capital Needs

We have incurred significant operating losses since inception and anticipate that we will continue to incur

substantial operating losses for the foreseeable future and may never achieve or maintain profitability.

Since inception in January 2016, we have incurred significant operating losses. Our net loss was $82.5 million and

$105.6 million for the years ended December 31, 2022 and 2021, respectively. As of December 31, 2022, we had an
accumulated deficit of $348.8 million. We expect to continue to incur significant expenses and increasing operating losses
for the foreseeable future. Since inception, we have devoted substantially all of our efforts to research and preclinical and
clinical development of our product candidates, organizing and staffing our company, business planning, raising capital,
establishing our intellectual property portfolio and conducting clinical trials. To date, we have never obtained regulatory
approval for, or commercialized, any drugs. It could be several years, if ever, before we have a commercialized drug. The
net losses we incur may fluctuate significantly from quarter to quarter and year-to-year. We anticipate that our expenses
will increase substantially if, and as, we:

● continue the ongoing and planned development of our product candidates;
● initiate, conduct and complete any ongoing, anticipated or future preclinical studies and clinical trials for our

current and future product candidates;

● seek marketing approvals for any product candidates that successfully complete clinical trials;
● establish a sales, marketing, manufacturing and distribution infrastructure to commercialize any current or

future product candidate for which we may obtain marketing approval;

● seek to discover and develop additional product candidates;
● continue to build a portfolio of product candidates through the acquisition or in-license of drugs, product

candidates or technologies;

● maintain, protect and expand our intellectual property portfolio;
● meet the requirements and demands of being a public company;
● defend against any product liability claims or other lawsuits related to our products;
● hire additional clinical, regulatory and scientific personnel; and
● add operational, financial and management information systems and personnel, including personnel to

support our product development and planned future commercialization efforts.

Furthermore, we have incurred additional costs associated with operating as a public company, including

significant legal, accounting, investor relations and other expenses.

To become and remain profitable, we must succeed in developing and eventually commercializing drugs that

generate significant revenue. This will require us to be successful in a range of challenging activities, including completing
preclinical studies and clinical trials of our current and future product candidates, obtaining regulatory approval, procuring
commercial-scale manufacturing, marketing and selling any products for which we obtain regulatory approval (including
through third parties), as well as discovering or acquiring and developing additional product candidates. We are only in the
preliminary stages of most of these activities. We may never succeed in these activities and, even if we do, may never
generate revenues that are sufficient to offset our expenses and achieve profitability.

Because of the numerous risks and uncertainties associated with drug development, we are unable to accurately

predict the timing or amount of expenses or when, or if, we will be able to achieve profitability. If we are required by
regulatory authorities to perform studies in addition to those currently expected, or if there are any delays in the initiation
and completion of our clinical trials or the development of any of our product candidates, our expenses could increase.

Even if we do achieve profitability, we may not be able to sustain or increase profitability on a quarterly or annual

basis. Our failure to become and remain profitable would decrease the value of our company and could impair our ability
to raise capital, maintain our research and development efforts, expand our business or continue our operations. A decline
in the value of our common stock could also cause you to lose all or part of your investment.

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The report of our independent registered public accounting firm included a "going concern" explanatory

paragraph.

The report of our independent registered public accounting firm on our financial statements for the year ended 
December 31, 2022 includes an explanatory paragraph regarding the existence of substantial doubt about our ability to 
continue as a going concern. Our cash and cash equivalents were $30.6 million at December 31, 2022. We also received a 
$10.7 million upfront payment from Advanz Pharma in January 2023 in conjunction with signing the exclusive licensing 
agreement for European commercialization rights.  We believe that our cash and cash equivalents as of December 31, 2022, 
along with the upfront payment received in January 2023 and the projected clinical and regulatory milestone payments 
expected in fiscal year 2023 from Advanz Pharma will be sufficient to fund our operations through year end 2023, and 
potentially beyond if clinical trial completion and marketing authorization in Europe as well as commercial sales 
milestones materialize in the expected timelines.  However, given our planned expenditures for the next several years, we 
have concluded, and our independent registered public accounting firm has agreed with our conclusion that there is still a 
substantial doubt regarding our ability to continue as a going concern for a period of 12 months beyond the filing of this 
Annual Report on Form 10-K. Any such inability to continue as a going concern may result in our stockholders losing their 
entire investment. There is no guarantee that we will become profitable or secure additional financing on acceptable terms.

Our limited operating history may make it difficult for you to evaluate the success of our business to date and

to assess our future viability.

We are a clinical-stage company with limited operational history, and our operations to date have been largely
focused on raising capital, organizing and staffing our company, identifying and developing our product candidates, and
undertaking preclinical and clinical development for our product candidates. As an organization, we have not yet
demonstrated an ability to successfully complete clinical development, obtain regulatory approvals, manufacture a
commercial-scale product or conduct sales and marketing activities necessary for successful commercialization, or arrange
for a third party to conduct these activities on our behalf. Consequently, any predictions about our future success or
viability may not be as accurate as they could be if we had a longer operating history.

We have encountered, and may continue to encounter unforeseen expenses, difficulties, complications, delays and

other known or unknown factors in achieving our business objectives. We will need to transition at some point from a
company with a research and development focus to a company capable of supporting commercial activities. We may not be
successful in such a transition.

Additionally, we expect our financial condition and operating results to continue to fluctuate from quarter to
quarter and year to year due to a variety of factors, many of which are beyond our control. Accordingly, you should not rely
upon the results of any quarterly or annual periods as indications of future operating performance.

We will require substantial additional funding to finance our operations. If we are unable to raise capital when

needed, we could be forced to delay, reduce or terminate certain of our development programs or other operations.

As of December 31, 2022, our cash, cash equivalents and marketable securities was $30.6 million. We also 
received a $10.7 million upfront payment from Advanz Pharma in January 2023  in conjunction with signing the exclusive 
licensing agreement for European commercialization rights. We believe that our cash and cash equivalents as of December 
31, 2022, along with the upfront payment received in January 2023 and the projected clinical and regulatory milestone 
payments expected in fiscal year 2023 from Advanz Pharma will be sufficient to fund our operations through year end 
2023, and potentially beyond if drug approvals materialize in the expected timelines. Based on our current operating and 
research and development plans, a substantial doubt exists regarding whether our existing cash, cash equivalents, and 
marketable securities will be sufficient to fund our projected operations through the next 12 months from the date the 
financial statements were issued. We will need to obtain substantial additional funding in connection with our continuing
operations and planned research and clinical development activities. Our future capital requirements will depend on many
factors, including:

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● the timing, progress and results of our ongoing preclinical studies and clinical trials of our product

candidates;

● the scope, progress, results and costs of preclinical development, laboratory testing and clinical trials of other

product candidates that we may pursue;

● our ability to establish collaborations on favorable terms, if at all;
● the costs, timing and outcome of regulatory review of our product candidates;
● the costs and timing of future commercialization activities, including product manufacturing, marketing,
sales and distribution, for any of our product candidates for which we receive marketing approval;
● the revenue, if any, received from commercial sales of our product candidates for which we receive

marketing approval;

● the cost of any milestone and royalty payments with respect to any approved product candidates;
● the costs and timing of preparing, filing and prosecuting patent applications, maintaining and enforcing our

intellectual property rights and defending any intellectual property-related claims;

● the costs of operating as a public company; and
● the extent to which we acquire or in-license other product candidates and technologies.

Identifying potential product candidates and conducting preclinical testing and clinical trials is a time-consuming,

expensive and uncertain process that takes years to complete, and we may never generate the necessary data or results
required to obtain regulatory approval and achieve product sales. In addition, our product candidates, if approved, may not
achieve commercial success. Our commercial revenues, if any, will be derived from sales of drugs that we do not expect to
be commercially available for several years, if at all. Accordingly, we will need to continue to rely on additional financing
to achieve our business objectives. We may seek additional capital due to favorable market conditions or strategic
considerations even if we believe we have sufficient funds for our current or future operating plans.

In addition, our ability to access additional capital has been affected by overall macroeconomic trends, among
other things, including rising interest rates, which have caused the price of our common stock to fluctuate significantly
and/or decline. These macroeconomic trends have been exacerbated by recent hostilities between Russia and Ukraine,
which have contributed to further economic instability in the global financial markets. As a result, adequate additional
financing may not be available to us when needed or on attractive terms. If we are unable to raise capital when needed or
on attractive terms, we could be forced to delay, reduce, or altogether terminate our research and development programs or
future commercialization efforts.

Raising additional capital may cause dilution to our stockholders and restrict our operations or require us to

relinquish rights to our product candidates.

Until such time, if ever, as we can generate substantial product revenue, we expect to finance our cash needs

through public or private equity or debt financings, including through the Cowen Equity Distribution Agreement, third
party funding, marketing and distribution arrangements, as well as other collaborations, strategic alliances and licensing
arrangements, or any combination of these approaches. We do not have any committed external source of funds. To the
extent that we raise additional capital through the sale of equity or convertible debt securities, your ownership interest in
our company may be diluted, and the terms of these securities may include liquidation or other preferences that adversely
affect your rights as a stockholder. Debt and equity financings, if available, may involve agreements that include covenants
limiting or restricting our ability to take specific actions, such as redeeming our shares, making investments, incurring
additional debt, making capital expenditures, declaring dividends or placing limitations on our ability to acquire, sell or
license intellectual property rights.

If we raise additional capital through future collaborations, strategic alliances or third party licensing
arrangements, we may have to relinquish valuable rights to our intellectual property, future revenue streams, research
programs or product candidates, or grant licenses on terms that may not be favorable to us. If we are unable to raise
additional capital when needed, we may be required to delay, limit, reduce or terminate our drug development or future
commercialization efforts, or grant rights to develop and market product candidates that we would otherwise develop and
market ourselves.

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Our ability to use our net operating losses to offset future taxable income may be subject to certain limitations.

We have incurred substantial losses since inception and do not expect to become profitable in the near future, if

ever. In general, under Section 382 of the United States Internal Revenue Code of 1986, as amended, or the Code, a
corporation that undergoes an “ownership change” is subject to limitations on its ability to utilize its pre-change NOLs to
offset future taxable income. We may have experienced ownership changes in the past and may experience ownership
changes in the future as a result of subsequent changes in our stock ownership (some of which shifts are outside our
control). As a result, if, and to the extent that we earn net taxable income, our ability to use our pre-change NOLs to offset
such taxable income may be subject to limitations.

For NOLs arising in tax years beginning after December 31, 2017, the Code limits a taxpayer’s ability to utilize

NOL carryforwards to 80% of taxable income. In addition, NOLs arising in tax years ending after December 31, 2017 can
be carried forward indefinitely, but carryback is generally prohibited. NOLs generated in tax years beginning before
January 1, 2018 will not be subject to the taxable income limitation, and NOLs generated in tax years ending before
January 1, 2018 will continue to have a two-year carryback and 20-year carryforward period. Deferred tax assets for NOLs
will need to be measured at the applicable tax rate in effect when the NOL is expected to be utilized. The limitations in the
carryforward/carryback periods, as well as the limitation on use of NOLs for NOLs arising in tax years beginning after
December 31, 2017 may significantly impact our ability to utilize our NOLs to offset taxable income in the future.

In order to realize the future tax benefits of our NOL carryforwards, we must generate taxable income, of which

there is no assurance. Accordingly, we have provided a full valuation allowance for deferred tax assets as of December 31,
2021 and 2022.

Risks Related to the Development and Commercialization of Our Product Candidates

Our future success is substantially dependent on the successful clinical development, regulatory approval and
commercialization of our product candidates. If we are not able to obtain required regulatory approvals, we will not be
able to commercialize our product candidates and our ability to generate product revenue will be adversely affected.

We have invested a significant portion of our time and financial resources in the development of AT-007, AT-001
and AT-003. Our business is dependent on our ability to successfully complete development of, obtain regulatory approval
for, and, if approved, successfully commercialize our product candidates in a timely manner. We may face unforeseen
challenges in our drug development strategy, and we can provide no assurances that our drug design will prove to be
effective, that we will be able to take advantage of expedited regulatory pathways for any of our product candidates, or that
we will ultimately be successful in our future clinical trials.

We have not obtained regulatory approval for any product candidate, and it is possible that any product candidates

we may seek to develop in the future will not obtain regulatory approval. Neither we nor any future collaborator is
permitted to market any product candidates in the United States or abroad until we receive regulatory approval from the
FDA or applicable foreign regulatory agency. The time required to obtain approval or other marketing authorizations by the
FDA and comparable foreign regulatory authorities is unpredictable and typically takes many years following the
commencement of clinical trials and depends upon numerous factors, including the substantial discretion of the regulatory
authorities. In addition, approval policies, regulations or the type and amount of clinical data necessary to gain approval
may change during the course of a product candidate’s clinical development and may vary among jurisdictions.

Prior to obtaining approval to commercialize any product candidate in the United States or abroad, we must
demonstrate with substantial evidence from well-controlled clinical trials, and to the satisfaction of the FDA or comparable
foreign regulatory authorities, that such product candidate is safe and effective for its intended uses. Results from
preclinical studies and clinical trials can be interpreted in different ways. Even if we believe that the preclinical or clinical
data for our product candidates are promising, such data may not be sufficient to support approval by the FDA

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and other regulatory authorities. The FDA may also require us to conduct additional preclinical studies or clinical trials for
our product candidates either prior to or post-approval, or it may object to elements of our clinical development program,
requiring their alteration.

Of the large number of products in development, only a small percentage successfully complete the FDA or

comparable foreign regulatory authorities approval processes and are commercialized. The lengthy approval or marketing
authorization process as well as the unpredictability of future clinical trial results may result in our failing to obtain
regulatory approval or marketing authorization to market our product candidates, which would significantly harm our
business, financial condition, results of operations and prospects.

Even if we eventually complete clinical testing and receive approval of a new drug application, or NDA, or
foreign marketing for our product candidates, the FDA or the comparable foreign regulatory authorities may grant approval
or other marketing authorization contingent on the performance of costly additional clinical trials, including post-market
clinical trials. The FDA or the comparable foreign regulatory authorities also may approve or authorize for marketing a
product candidate for a more limited indication or patient population than we originally request, and the FDA or
comparable foreign regulatory authorities may not approve or authorize the labeling that we believe is necessary or
desirable for the successful commercialization of a product candidate. Any delay in obtaining, or inability to obtain,
applicable regulatory approval or other marketing authorization would delay or prevent commercialization of that product
candidate and would adversely impact our business and prospects.

In addition, the FDA or comparable foreign regulatory authorities may change their policies, adopt additional

regulations or revise existing regulations or take other actions, which may prevent or delay approval of our future product
candidates under development on a timely basis. Such policy or regulatory changes could impose additional requirements
upon us that could delay our ability to obtain approvals, increase the costs of compliance or restrict our ability to maintain
any marketing authorizations we may have obtained.

Furthermore, even if we obtain regulatory approval for our product candidates, we will still need to develop a

commercial organization, establish a commercially viable pricing structure and obtain approval for coverage and adequate
reimbursement from third party and government payors, including government health administration authorities. If we are
unable to successfully commercialize our product candidates, we may not be able to generate sufficient revenue to continue
our business.

We or Advanz Pharma may fail to perform under any of the agreements entered into in connection with the

partnership for commercialization of AT-007, which may subject us to liabilities, and we may fail to achieve anticipated
benefits of the partnership.

In January 2023, we announced a partnership with Advanz Pharma (“Advanz”) for commercialization of AT-007

(govorestat) in Europe, and entered into an Exclusive License and Supply Agreement (the “Advanz Agreement”) with
Advanz. Under the terms of the Advanz Agreement, Advanz receives exclusive commercial rights in the European
Economic Area, Switzerland, and the UK (the “Territory”) for AT-007 in Galactosemia and SORD Deficiency, with certain
rights to future indications for AT-007 in the Territory. In return, we have the right to receive certain near-term development
milestone payments upon clinical trial completion and marketing authorization in Europe as well as commercial sales
milestones, which in the aggregate are expected to amount to over €130 million. We also have the right to receive royalties
on any future net sales of AT-007 in the Territory of 20%. The royalty rate will be payable on a country-by-country basis
until the later of (i) the expiration of the licensed patents covering the composition of matter of AT-007, or (ii) 10 years
after the European Medicines Agency’s grant of marketing authorization for AT-007. The royalties are subject to certain
deductions, including certain secondary finishing costs, certain step-in establishment costs and a portion of fees for any
potential third party patent licenses if applicable in the future. Following the initial term of the license, as described above,
the royalty rate shall be reduced to 10% and shall continue in perpetuity unless the Advanz Agreement is terminated in
various circumstances in accordance with its terms. We will continue to be responsible for the development, manufacturing
and supply of AT-007, and Advanz will be responsible for packaging, distribution and commercialization in the Territory.
The Advanz Agreement includes a sublicense under the 2016 Columbia Agreement and the 2020 Miami License
Agreement.

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Our partnership with Advanz is subject to various risks, including but not limited to the following:

● If Advanz breaches the contractual obligations owed to us pursuant to the Advanz Agreement or any related

agreements, we could be exposed to commercial, regulatory or other liabilities.

● We may be subject to liabilities in connection with the development, manufacturing and supply of AT-007
● under the Advanz Agreement, including with respect to the 2016 Columbia Agreement and the 2020 Miami

License Agreement.

● We may not be able to adequately protect our intellectual property or may become involved in intellectual

property enforcement actions, which may cause us to incur substantial costs as a result of litigation or other
proceedings relating to patent and other intellectual property rights, and such litigation may divert the attention of
our management and scientific personnel and adversely affect our development and commercialization efforts.
● We may have limited control over the commercialization efforts of Advanz, and Advanz may fail to successfully

sell and market AT-007.

● Our ability to receive certain economic benefits from the partnership, including the milestone payments and

royalties, depends on certain contingencies beyond our control.

● In certain circumstances, Advanz may exercise certain step-in rights, including the ability for Advanz to perform
its own supply arrangements, and in some cases, specified development rights in the Territory and assignment of
certain contract rights. In all such circumstances, Advanz must continue to pay royalties and milestone payments,
but may recoup certain of its manufacturing and development establishment costs, and deduct such costs from
royalties owed.

Any of these factors could cause us to incur higher costs, disrupt the supply of our product candidates or approved

products, delay the approval of our product candidates or prevent or disrupt the commercialization of our approved
products. As a result, we may not achieve some or all economic benefits expected from the partnership.

The development of additional product candidates is risky and uncertain, and we can provide no assurances

that we will be able to replicate our approach to drug development for other disease indications.

Efforts to identify, acquire or in-license, and then develop, product candidates require substantial technical,

financial and human resources, whether or not any product candidates are ultimately identified. Our efforts may initially
show promise in identifying potential product candidates, yet fail to yield product candidates for clinical development,
approved products or commercial revenues for many reasons, including the following:

● the methodology used may not be successful in identifying potential product candidates;
● competitors may develop alternatives that render any product candidates we develop obsolete;
● any product candidates we develop may be covered by third parties’ patents or other exclusive rights;
● a product candidate may be shown to have harmful side effects or other characteristics that indicate it is

unlikely to be effective or otherwise does not meet applicable regulatory criteria;

● a product candidate may not be capable of being produced in commercial quantities at an acceptable cost, or

at all; and

● a product candidate may not be accepted as safe and effective by physicians, patients, the medical

community or third party payors.

We have limited financial and management resources and, as a result, we may forego or delay pursuit of
opportunities with other product candidates or for other indications that later prove to have greater market potential. Our
resource allocation decisions may cause us to fail to capitalize on viable commercial drugs or profitable market
opportunities. If we do not accurately evaluate the commercial potential or target market for a particular product candidate,
we may relinquish valuable rights to that product candidate through collaboration, licensing or other royalty arrangements
in circumstances under which it would have been more advantageous for us to retain sole development and
commercialization rights to such product candidate. In addition, we may not be successful in replicating our approach to
drug development for other disease indications. If we are unsuccessful in identifying and developing additional product
candidates or are unable to do so, our business may be harmed.

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Success in preclinical studies or earlier clinical trials may not be indicative of results in future clinical trials

and we cannot assure you that any ongoing, planned or future clinical trials will lead to results sufficient for the
necessary regulatory approvals.

Success in preclinical testing and earlier clinical trials does not ensure that later clinical trials will generate the

same results or otherwise provide adequate data to demonstrate the efficacy and safety of a product candidate. Preclinical
studies and Phase 1 clinical trials are primarily designed to test safety, to study pharmacokinetics and pharmacodynamics
and to understand the side effects of product candidates at various doses and schedules. Success in preclinical studies and
earlier clinical trials does not ensure that later efficacy trials will be successful, nor does it predict final results. Our product
candidates may fail to show the desired safety and efficacy in clinical development despite positive results in preclinical
studies or having successfully advanced through earlier clinical trials.

In addition, the design of a clinical trial can determine whether its results will support approval of a product, and
flaws in the design of a clinical trial may not become apparent until the clinical trial is well advanced. As an organization,
we have limited experience designing clinical trials and may be unable to design and execute a clinical trial to support
regulatory approval. Many companies in the pharmaceutical and biotechnology industries have suffered significant
setbacks in late-stage clinical trials even after achieving promising results in preclinical testing and earlier clinical trials.
Data obtained from preclinical and clinical activities are subject to varying interpretations, which may delay, limit or
prevent regulatory approval. In addition, we may experience regulatory delays or rejections as a result of many factors,
including changes in regulatory policy during the period of our product candidate development. Any such delays could
negatively impact our business, financial condition, results of operations and prospects.

Clinical drug development involves a lengthy and expensive process. We may incur additional costs and

encounter substantial delays or difficulties in our clinical trials.

We may not commercialize, market, promote or sell any product candidate without obtaining marketing approval

from the FDA or other comparable regulatory authority, and we may never receive such approvals. It is impossible to
predict when or if any of our product candidates will prove effective or safe in humans and will receive regulatory
approval. Before obtaining marketing approval from regulatory authorities for the sale of our product candidates, we must
complete preclinical development and then conduct extensive clinical trials to demonstrate the safety and efficacy of our
product candidates in humans. Clinical testing is expensive, is difficult to design and implement, can take many years to
complete and is uncertain as to outcome.

A failure of one or more clinical trials can occur at any stage of testing. Moreover, preclinical and clinical data are

often susceptible to varying interpretations and analyses, and many companies that have believed their product candidates
performed satisfactorily in preclinical studies and clinical trials have nonetheless failed to obtain marketing approval of
their products.

We may experience numerous unforeseen events prior to, during, or as a result of, clinical trials that could delay or

prevent our ability to receive marketing approval or commercialize our product candidates, including the following:

● delays in reaching a consensus with regulatory authorities on the design or implementation of our clinical

trials;

● regulators or institutional review boards, or IRBs, may not authorize us or our investigators to commence a

clinical trial or conduct a clinical trial at a prospective trial site;

● delays in reaching agreement on acceptable terms with prospective clinical research organizations, or CROs,

and clinical trial sites;

● the number of patients required for clinical trials of our product candidates may be larger than we anticipate,
enrollment in these clinical trials may be slower than we anticipate, participants may drop out of these
clinical trials at a higher rate than we anticipate or fail to return for post-treatment follow-up or we may fail
to recruit suitable patients to participate in a trial;

● clinical trials of our product candidates may produce negative or inconclusive results;

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● imposition of a clinical hold by regulatory authorities as a result of a serious adverse event, concerns with a
class of product candidates or after an inspection of our clinical trial operations, trial sites or manufacturing
facilities;

● occurrence of serious adverse events associated with the product candidate that are viewed to outweigh its

potential benefits;

● changes in regulatory requirements and guidance that require amending or submitting new clinical protocols;

or

● we may decide, or regulators may require us, to conduct additional clinical trials or abandon product

development programs.

Any inability to successfully complete preclinical and clinical development could result in additional costs to us or

impair our ability to generate revenue from future drug sales or other sources. In addition, if we make manufacturing or
formulation changes to our product candidates, we may need to conduct additional testing to bridge our modified product
candidate to earlier versions. Clinical trial delays could also shorten any periods during which we may have the exclusive
right to commercialize our product candidates, if approved, or allow our competitors to bring competing drugs to market
before we do, which could impair our ability to successfully commercialize our product candidates and may harm our
business, financial condition, results of operations and prospects.

Additionally, if the results of our clinical trials are inconclusive or if there are safety concerns or serious adverse

events associated with our product candidates, we may:

● be delayed in obtaining marketing approval, or not obtain marketing approval at all;
● obtain approval for indications or patient populations that are not as broad as intended or desired;
● obtain approval with labeling that includes significant use or distribution restrictions or safety warnings,

including in the form of a risk evaluation and mitigation strategy, or REMS;

● be subject to additional post-marketing testing requirements;
● be required to perform additional clinical trials to support approval or be subject to additional post-marketing

testing requirements;

● have regulatory authorities withdraw, or suspend, their approval of the drug or impose restrictions on its

distribution in the form of a modified REMS;

● be subject to the addition of labeling statements, such as warnings or contraindications;
● be sued; or
● experience damage to our reputation.

Our product development costs will also increase if we experience delays in testing or obtaining marketing
approvals. We do not know whether any of our preclinical studies or clinical trials will begin as planned, need to be
restructured or be completed on schedule, if at all.

Further, we, the FDA or an IRB may suspend our clinical trials at any time if it appears that we or our
collaborators are failing to conduct a trial in accordance with regulatory requirements, including the FDA’s current Good
Clinical Practice, or GCP, regulations, that we are exposing participants to unacceptable health risks, or if the FDA finds
deficiencies in our investigational new drug applications, or INDs, or the conduct of these trials. Therefore, we cannot
predict with any certainty the schedule for commencement and completion of future clinical trials. If we experience delays
in the commencement or completion of our clinical trials, or if we terminate a clinical trial prior to completion, the
commercial prospects of our product candidates could be negatively impacted, and our ability to generate revenues from
our product candidates may be delayed.

All of our current product candidates that have proceeded to clinical trials target inhibition of aldose reductase.

There can be no assurance that aldose reductase inhibitors will ever receive regulatory approval.

All of our current product candidates that have proceeded to clinical trials target inhibition of the aldose reductase
enzyme. There are no currently approved aldose reductase inhibitors on the market outside of Japan, India and China, and
there can be no assurance that aldose reductase inhibitors will ever receive regulatory approval in all other

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countries, including the United States. Prior attempts to inhibit this enzyme were hindered by nonselective, nonspecific
inhibition, which resulted in limited efficacy and significant off-target safety effects. Our current product candidates,
including AT-007, AT-001 and AT-003, may face similar or different challenges that prevent their successful
commercialization.

We may not be able to obtain or maintain rare pediatric disease designation or exclusivity for our product

candidates, which could limit the potential profitability of our product candidates.

We have obtained orphan drug designation and rare pediatric disease designation, from the FDA for AT-007 for

the treatment of Galactosemia and PMM2-CDG. The FDA may grant orphan drug designation to a drug intended to treat a
rare disease or condition, which is defined as a disease or condition that either affects fewer than 200,000 individuals in the
United States, or if it affects more than 200,000 individuals, there is no reasonable expectation that sales of the drug in the
United States will be sufficient to offset the costs of developing and making the drug available in the United States. Orphan
drug designation does not convey any advantage in, or shorten the duration of, the regulatory review and approval process.

For the purposes of the rare pediatric disease program, a “rare pediatric disease” is a serious or life-threatening

disease in which the serious or life-threatening manifestations primarily affect individuals aged from birth to 18 years or a
rare disease or conditions within the meaning of the Orphan Drug Act. Under the FDA’s rare pediatric disease priority
review voucher, or RPD-PRV, program, upon the approval of an NDA for the treatment of a rare pediatric disease, the
sponsor of such application would be eligible for an RPD-PRV that can be used to obtain priority review for a subsequent
NDA. The sponsor of the application may transfer (including by sale) the RPD-PRV to another sponsor. The voucher may
be further transferred any number of times before the voucher is used, as long as the sponsor making the transfer has not
yet submitted the application. Congress has extended the RPD-PRV program until September 30, 2024, with potential for
vouchers to be granted until 2026. This program has been subject to criticism, including by the FDA. As such it is possible
that even though we have obtained qualification for a RPD-PRV, the program may no longer be in effect at the time of
approval. Also, although priority review vouchers may be sold or transferred to third parties, there is no guaranty that we
will be able to realize any value if we obtained, and subsequently were able to sell a priority review voucher. The RPD-
PRV program is currently scheduled to sunset as of September 30, 2026.

A breakthrough therapy designation by the FDA for a product candidate may not lead to a faster development

or regulatory review or approval process, and it would not increase the likelihood that the product candidate will receive
marketing approval.

We may seek a breakthrough therapy designation for one or more product candidates. A breakthrough therapy is
defined as a product candidate that is intended, alone or in combination with one or more other drugs, to treat a serious or
life-threatening disease or condition, and preliminary clinical evidence indicates that the product candidate may
demonstrate substantial improvement over existing therapies on one or more clinically significant endpoints, such as
substantial treatment effects observed early in clinical development. For product candidates that have been designated as
breakthrough therapies, interaction and communication between the FDA and the sponsor of the trial can help to identify
the most efficient path for clinical development while minimizing the number of patients placed in ineffective control
regimens. Product candidates designated as breakthrough therapies by the FDA are also eligible for priority review if
supported by clinical data at the time of the submission of the NDA.

Designation as a breakthrough therapy is within the discretion of the FDA. Accordingly, even if we believe that

one of our product candidates meets the criteria for designation as a breakthrough therapy, the FDA may disagree and
instead determine not to make such designation. In any event, the receipt of a breakthrough therapy designation for a
product candidate may not result in a faster development process, review or approval compared to product candidates
considered for approval under conventional FDA procedures and it would not assure ultimate approval by the FDA. In
addition, even if one or more of our product candidates qualify as breakthrough therapies, the FDA may later decide that
the product candidate no longer meets the conditions for qualification or it may decide that the time period for FDA review
or approval will not be shortened.

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We have sought, and may in the future seek, fast track designation from the FDA for our product candidates.

Even if granted, fast track designation may not actually lead to a faster development, regulatory review or approval
process.

If a product candidate is intended for the treatment of a serious or life-threatening condition and demonstrates the

potential to address unmet needs for this condition, the sponsor may apply for FDA fast track designation. If fast track
designation is obtained, the FDA may prioritize interactions with the sponsor concerning the designated development
program and initiate review of sections of an NDA before the application is complete, known as “rolling review.” Fast
track designation would not ensure that we would experience a faster development, regulatory review or approval process
compared to conventional FDA procedures or that we would ultimately obtain regulatory approval. Additionally, the FDA
may withdraw fast track designation if it believes that the designation is no longer supported by data from our clinical
development program.

We intend to seek approval from the FDA through the use of accelerated registration pathways. If we are

unable to obtain approval under an accelerated pathway, we may be required to conduct additional preclinical studies
or clinical trials, which could increase the expense of obtaining, reduce the likelihood of obtaining and/or delay the
timing of obtaining, necessary marketing approvals. Even if we receive approval from the FDA to utilize an accelerated
registration pathway, if our confirmatory trials do not verify clinical benefit, or if we do not comply with rigorous post-
marketing requirements, the FDA may seek to withdraw accelerated approval.

We intend to seek an accelerated approval development pathway for our product candidates. Under the accelerated
approval provisions of the Federal Food, Drug, and Cosmetic Act, or the FDCA, and the FDA’s implementing regulations,
the FDA may grant accelerated approval to a product designed to treat a serious or life-threatening condition that provides
meaningful therapeutic advantage over available therapies and demonstrates an effect on a surrogate endpoint or
intermediate clinical endpoint that is reasonably likely to predict clinical benefit. The FDA considers a clinical benefit to be
a positive therapeutic effect that is clinically meaningful in the context of a given disease. For the purposes of accelerated
approval, a surrogate endpoint is a marker, such as a laboratory measurement, radiographic image, physical sign or other
measure that is thought to predict clinical benefit, but is not itself a measure of clinical benefit. An intermediate clinical
endpoint is a clinical endpoint that can be measured earlier than an effect on irreversible morbidity or mortality that is
reasonably likely to predict an effect on irreversible morbidity or mortality or other clinical benefit. The accelerated
approval development pathway may be used in cases in which the advantage of a new drug over available therapy may not
be a direct therapeutic advantage, but is a clinically important improvement from a patient and public health perspective. If
granted, accelerated approval is contingent on the sponsor’s agreement to conduct, in a diligent manner, additional post-
approval confirmatory studies to verify and describe the drug’s clinical profile or risks and benefits for accelerated
approval. The FDA may require that any such confirmatory studies be initiated or substantially underway prior to the
submission of an application for accelerated approval. If such post-approval studies fail to confirm the drug’s clinical
profile or risks and benefits, the FDA may withdraw its approval of the drug. FDORA made amendments to the accelerated
approval program, among them new requirements relating to post-approval studies and enhanced enforcement and
withdrawal authorities for the FDA, including in the event that a sponsor fails to comply with applicable requirements
under the program. Because we are still in early stages of our clinical trials, we can provide no assurances that our
biomarker-based approach will be successful in demonstrating a causal link to the relevant outcomes we are evaluating. If
our approach is not successful, we may be required to conduct longer clinical trials.

If we choose to pursue accelerated approval, we intend to seek feedback from the FDA or will otherwise evaluate

our ability to seek and receive such accelerated approval. There can be no assurance that, after our evaluation of the
feedback from the FDA or other factors, we will decide to pursue or submit an NDA for accelerated approval or any other
form of expedited development, review or approval. Furthermore, even if we submit an application for accelerated
approval, there can be no assurance that the application will be accepted or that approval will be granted on a timely basis,
or at all. The FDA also could require us to conduct further studies or trials prior to considering our application or granting
approval of any type. We might not be able to fulfill the FDA’s requirements in a timely manner, which would cause
delays, or approval might not be granted because our submission is deemed incomplete by the FDA. A failure to obtain
accelerated approval or any other form of expedited development, review or approval for a product candidate would result
in a longer time period to commercialize such product candidate, could increase the cost of development of such product
candidate and could harm our competitive position in the marketplace.

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Even if we receive accelerated approval from the FDA, we will be subject to rigorous post-marketing
requirements, including the completion of confirmatory post-market clinical trial(s) to verify the clinical benefit of the
product, and submission to the FDA of all promotional materials prior to their dissemination. The FDA could seek to
withdraw accelerated approval for multiple reasons, including if we fail to conduct any required post-market study with
due diligence, a post-market study does not confirm the predicted clinical benefit, other evidence shows that the product is
not safe or effective under the conditions of use, or we disseminate promotional materials that are found by the FDA to be
false or misleading.

A failure to obtain accelerated approval or any other form of expedited development, review or approval for a

product candidate that we may choose to develop would result in a longer time period prior to commercializing such
product candidate, could increase the cost of development of such product candidate and could harm our competitive
position in the marketplace.

Enrollment and retention of patients in clinical trials is an expensive and time-consuming process and could be

delayed, made more difficult or rendered impossible by multiple factors outside our control.

Identifying and qualifying patients to participate in our clinical trials is critical to our success. We may encounter

difficulties in enrolling patients in our clinical trials, thereby delaying or preventing development and approval of our
product candidates. Even once enrolled, we may be unable to retain a sufficient number of patients to complete any of our
trials. Patient enrollment and retention in clinical trials depends on many factors, including the size of the patient
population, the nature of the trial protocol, the existing body of safety and efficacy data, the number and nature of
competing treatments and ongoing clinical trials of competing therapies for the same indication, the proximity of patients
to clinical sites and the eligibility criteria for the trial. Because our focus includes rare disorders, there are limited patient
pools from which to draw in order to complete our clinical trials in a timely and cost-effective manner. Accordingly,
enrollment of our clinical trials could take significantly longer than projected, which would delay any potential approval of
our product candidates. Furthermore, even if we are able to enroll a sufficient number of patients for our clinical trials, we
may have difficulty maintaining enrollment of such patients in our clinical trials.

Our efforts to build relationships with patient communities may not succeed, which could result in delays in

patient enrollment in our clinical trials. Any negative results we may report in clinical trials of our product candidates may
make it difficult or impossible to recruit and retain patients in other clinical trials of that same product candidate. Delays or
failures in planned patient enrollment or retention may result in increased costs, program delays or both, which could have
a harmful effect on our ability to develop our product candidates or could render further development impossible. In
addition, we may rely on CROs and clinical trial sites to ensure proper and timely conduct of our future clinical trials and,
while we intend to enter into agreements governing their services, we will be limited in our ability to ensure their actual
performance.

For additional information regarding delays in enrollment and retention of patients, see “Risks Related to Our

Business Operations, Employee Matters and Managing Growth—Our business may be adversely affected by the
coronavirus outbreak.”

Our product candidates may cause undesirable side effects or have other properties that could delay or prevent
their regulatory approval, limit their commercial potential or result in significant negative consequences following any
potential marketing approval.

During the conduct of clinical trials, patients report changes in their health, including illnesses, injuries and
discomforts, to their doctor. Often, it is not possible to determine whether or not the product candidate being studied caused
these conditions. Regulatory authorities may draw different conclusions or require additional testing to confirm these
determinations, if they occur.

In addition, it is possible that as we test our product candidates in larger, longer and more extensive clinical trials,

or as use of these product candidates becomes more widespread if they receive regulatory approval, illnesses, injuries,
discomforts and other adverse events that were observed in earlier trials, as well as conditions that did not occur or went
undetected in previous trials, will be reported by subjects or patients. Many times, side effects are only

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detectable after investigational drugs are tested in large-scale pivotal trials or, in some cases, after they are made available
to patients on a commercial scale after approval. If additional clinical experience indicates that any of our product
candidates have side effects or cause serious or life-threatening side effects, the development of the product candidate may
fail or be delayed, or, if the product candidate has received regulatory approval, such approval may be revoked, which
would harm our business, prospects, operating results and financial condition.

Interim, “top-line” and preliminary data from our clinical trials that we announce or publish from time to time
may change as more patient data become available and are subject to audit and verification procedures that could result
in material changes in the final data.

From time to time, we may publish interim, “top-line” or preliminary data from our clinical trials. Interim data
from clinical trials that we may complete are subject to the risk that one or more of the clinical outcomes may materially
change as patient enrollment continues and more patient data become available. Preliminary or “top-line” data also remain
subject to audit and verification procedures that may result in the final data being materially different from the preliminary
data we previously published. As a result, interim and preliminary data should be viewed with caution until the final data
are available. Differences between preliminary or interim data and final data could significantly harm our business
prospects and may cause the trading price of our common stock to fluctuate significantly.

The incidence and prevalence for target patient populations of our product candidates have not been
established with precision. If the market opportunities for our product candidates are smaller than we believe they are
or any approval we obtain is based on a narrower definition of the patient population, our business may suffer.

We currently focus our drug development on product candidates for the treatment of diseases with high unmet

medical need. Our eligible patient population and pricing estimates may differ significantly from the actual market
addressable by our product candidates. Our estimates of both the number of people who have these diseases, as well as the
subset of people with these diseases who have the potential to benefit from treatment with our product candidates, are
based on our beliefs and analyses. These estimates have been derived from a variety of sources, including the scientific
literature, patient foundations or market research, and may prove to be incorrect. Further, new studies may change the
estimated incidence or prevalence of the diseases we are targeting. The number of patients may turn out to be lower than
expected. Likewise, the potentially addressable patient population for each of our product candidates may be limited or
may not be receptive to treatment with our product candidates, and new patients may become increasingly difficult to
identify or access. If the market opportunities for our product candidates are smaller than we estimate, we may not be able
to achieve our forecast revenue, which could hinder our business plan and adversely affect our business and results of
operations.

We may face substantial competition, which may result in others developing or commercializing drugs before

or more successfully than us.

The development and commercialization of new drugs is highly competitive. We may face potential competition
with respect to our current product candidates and may face competition with respect to any other product candidates that
we may seek to develop or commercialize in the future from pharmaceutical and biotechnology companies, academic
institutions, government agencies and other public and private research institutions.

Our competitors may have an advantage over us due to their greater size, resources and institutional experience. In

particular, these companies have greater experience and expertise in securing reimbursement, government contracts and
relationships with key opinion leaders, conducting testing and clinical trials, obtaining and maintaining regulatory
approvals and distribution relationships to market products and marketing approved drugs. These companies also have
significantly greater research and marketing capabilities than we do. If we are not able to compete effectively against
existing and potential competitors, our business and financial condition may be harmed.

As a result of these factors, our competitors may obtain regulatory approval of their drugs before we are able to,

which may limit our ability to develop or commercialize our product candidates. Our competitors may also develop
therapies that are safer, more effective, more widely accepted or less expensive than ours, and may also be more successful
than we are in manufacturing and marketing their drugs. These advantages could render our product

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candidates obsolete or non-competitive before we can recover the costs of such product candidates’ development and
commercialization.

Mergers and acquisitions in the pharmaceutical and biotechnology industries may result in even more resources
being concentrated among a smaller number of our competitors. Smaller and early-stage companies may also prove to be
significant competitors, particularly through collaborative arrangements with large and established companies. These third-
parties compete with us in recruiting and retaining qualified scientific, management and commercial personnel,
establishing clinical trial sites and subject registration for clinical trials, as well as in acquiring technologies
complementary to, or necessary for, our programs.

We may explore strategic collaborations that may never materialize or we may be required to relinquish

important rights to and control over the development and commercialization of our product candidates to any future
collaborators.

Over time, our business strategy includes acquiring or in-licensing additional product candidates for treatments of

diseases with high unmet medical need. As a result, we intend to periodically explore a variety of possible strategic
collaborations in an effort to gain access to additional product candidates or resources. These strategic collaborations may
include partnerships with large strategic partners, particularly for the development of DPN treatments using AT-001. At the
current time however, we cannot predict what form such a strategic collaboration might take. We are likely to face
significant competition in seeking appropriate strategic collaborators, and strategic collaborations can be complicated and
time consuming to negotiate and document. We may not be able to negotiate strategic collaborations on acceptable terms,
or at all. We are unable to predict when, if ever, we will enter into any strategic collaborations because of the numerous
risks and uncertainties associated with establishing them.

Future collaborations could subject us to a number of risks, including:

● we may be required to undertake the expenditure of substantial operational, financial and management

resources;

● we may be required to issue equity securities that would dilute our stockholders’ percentage ownership of our

company;

● we may be required to assume substantial actual or contingent liabilities;
● we may not be able to control the amount and timing of resources that our strategic collaborators devote to

the development or commercialization of our product candidates;

● strategic collaborators may select indications or design clinical trials in a way that may be less successful

than if we were doing so;

● strategic collaborators may delay clinical trials, provide insufficient funding, terminate a clinical trial or
abandon a product candidate, repeat or conduct new clinical trials or require a new version of a product
candidate for clinical testing;

● strategic collaborators may not pursue further development and commercialization of products resulting from
the strategic collaboration arrangement or may elect to discontinue research and development programs;
● strategic collaborators may not commit adequate resources to the marketing and distribution of our product

candidates, limiting our potential revenues from these products;

● disputes may arise between us and our strategic collaborators that result in the delay or termination of the
research, development or commercialization of our product candidates or that result in costly litigation or
arbitration that diverts management’s attention and consumes resources;

● strategic collaborators may experience financial difficulties;
● strategic collaborators may not properly maintain, enforce or defend our intellectual property rights or may

use our proprietary information in a manner that could jeopardize or invalidate our proprietary information or
expose us to potential litigation;

● business combinations or significant changes in a strategic collaborator’s business strategy may adversely

affect a strategic collaborator’s willingness or ability to complete its obligations under any arrangement;

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● strategic collaborators could decide to move forward with a competing product candidate developed either

independently or in collaboration with others, including our competitors; and

● strategic collaborators could terminate the arrangement or allow it to expire, which would delay the

development and may increase the cost of developing our product candidates.

Even if any product candidates receive marketing approval, they may fail to achieve market acceptance by

physicians, patients, third party payors or others in the medical community necessary for commercial success.

Even if any product candidates receive marketing approval, they may fail to gain market acceptance by
physicians, patients, third party payors and others in the medical community. If such product candidates do not achieve an
adequate level of acceptance, we may not generate significant drug revenue and may not become profitable. The degree of
market acceptance of any product candidate, if approved for commercial sale, will depend on a number of factors,
including but not limited to:

● the convenience and ease of administration compared to alternative treatments and therapies;
● the willingness of the target patient population to try new therapies and of physicians to prescribe these

therapies;

● the efficacy and potential advantages compared to alternative treatments and therapies;
● the effectiveness of sales and marketing efforts;
● the strength of our relationships with patient communities;
● the cost of treatment in relation to alternative treatments and therapies, including any similar generic

treatments;

● our ability to offer such drug for sale at competitive prices;
● the strength of marketing and distribution support;
● the availability of third party coverage and adequate reimbursement;
● the prevalence and severity of any side effects; and
● any restrictions on the use of the drug together with other medications.

Our efforts to educate physicians, patients, third-party payors and others in the medical community on the benefits

of our product candidates may require significant resources and may never be successful. Such efforts may require more
resources than are typically required due to the complexity and uniqueness of our product candidates. Because we expect
sales of our product candidates, if approved, to generate substantially all of our revenues for the foreseeable future, the
failure of our product candidates to find market acceptance would harm our business.

Even if we obtain regulatory approvals for our product candidates, they will remain subject to ongoing

regulatory oversight.

Even if we obtain regulatory approvals for our product candidates, such approvals will be subject to ongoing

regulatory requirements for manufacturing, labeling, packaging, storage, advertising, promotion, sampling, record keeping
and submission of safety and other post-market information. Any regulatory approvals that we receive for our product
candidates may also be subject to a REMS, limitations on the approved indicated uses for which the drug may be marketed
or to the conditions of approval, or contain requirements for potentially costly post-marketing testing, including Phase 4
trials, and surveillance to monitor the quality, safety and efficacy of the drug. Such regulatory requirements may differ
from country to country depending on where we have received regulatory approval.

In addition, drug manufacturers and their facilities are subject to payment of user fees and continual review and

periodic inspections by the FDA and other regulatory authorities for compliance with current good manufacturing
practices, or cGMP, requirements and adherence to commitments made in the NDA or foreign marketing application. If we,
or a regulatory authority, discover previously unknown problems with a drug, such as adverse events of unanticipated
severity or frequency, or problems with the facility where the drug is manufactured or if a regulatory authority disagrees
with the promotion, marketing or labeling of that drug, a regulatory authority may impose restrictions relative to that drug,
the manufacturing facility or us, including requesting a recall or requiring withdrawal of the drug from the market or
suspension of manufacturing.

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If we fail to comply with applicable regulatory requirements following approval of our product candidates, a

regulatory authority may, among other actions:

● issue an untitled letter or warning letter asserting that we are in violation of the law;
● seek an injunction or impose administrative, civil or criminal penalties or monetary fines;
● suspend or withdraw regulatory approval;
● suspend any ongoing clinical trials;
● refuse to approve a pending NDA or comparable foreign marketing application or any supplements thereto

submitted by us or our partners;

● restrict the marketing or manufacturing of the drug;
● seize or detain the drug or otherwise require the withdrawal of the drug from the market;
● refuse to permit the import or export of product candidates; or
● refuse to allow us to enter into supply contracts, including government contracts.

Moreover, the FDA strictly regulates the promotional claims that may be made about drug products. In particular,
a product may not be promoted for uses that are not approved by the FDA as reflected in the product’s approved labeling.
The FDA and other agencies actively enforce the laws and regulations prohibiting the promotion of off-label uses, and a
company that is found to have improperly promoted off-label uses may be subject to significant civil, criminal and
administrative penalties.

Any government investigation of alleged violations of law could require us to expend significant time and

resources in response and could generate negative publicity. The occurrence of any event or penalty described above may
inhibit our ability to commercialize our product candidates and harm our business, financial condition, results of operations
and prospects.

The FDA’s and other regulatory authorities’ policies may change and additional laws or government regulations

may be enacted that could prevent, limit or delay regulatory approval of our product candidates. If we are not able to
maintain regulatory compliance with the FDCA, Cures Act, or other applicable requirements, we may lose any marketing
approval that we may have obtained and we may not achieve or sustain profitability, which would adversely affect our
business, prospects, financial condition and results of operations.

In addition, we cannot predict the likelihood, nature or extent of government regulation that may arise from future

legislation or administrative or executive action, either in the United States or abroad. For example, certain policies of the
U.S. administration may impact our business and industry. It is difficult to predict how executive actions, including
executive orders, may be implemented and the extent to which they will affect the FDA’s ability to exercise its regulatory
authority. If executive actions impose constraints on the FDA’s ability to engage in oversight and implementation activities
in the normal course, our business may be negatively impacted.

If we are unable to establish sales and marketing capabilities or enter into agreements with third parties to

market and sell our product candidates, we may not be successful in commercializing them, if and when they are
approved.

To successfully commercialize any product candidate that may result from our development programs, we will

need to build out our sales and marketing capabilities, either on our own or with others. The establishment and
development of our own commercial team or the establishment of a contract sales force to market any product candidate
we may develop will be expensive and time-consuming and could delay any drug launch. Moreover, we cannot be certain
that we will be able to successfully develop this capability. We may seek to enter into collaborations with other entities to
utilize their established marketing and distribution capabilities, but we may be unable to enter into such agreements on
favorable terms, if at all. If any current or future collaborators do not commit sufficient resources to commercialize our
product candidates, or we are unable to develop the necessary capabilities on our own, we may be unable to generate
sufficient revenue to sustain our business. We compete with many companies that currently have extensive, experienced
and well-funded marketing and sales operations to recruit, hire, train and retain marketing and sales personnel. We will
likely also face competition if we seek third parties to assist us with the sales and marketing

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efforts of our product candidates. Without an internal team or the support of a third party to perform marketing and sales
functions, we may be unable to compete successfully against these more established companies.

Even if we obtain and maintain approval for our product candidates from the FDA, we may never obtain

approval outside the United States, which would limit our market opportunities.

Approval of a product candidate in the United States by the FDA does not ensure approval of such product

candidate by regulatory authorities in other countries or jurisdictions, and approval by one foreign regulatory authority
does not ensure approval by regulatory authorities in other foreign countries or by the FDA. Sales of our product
candidates outside the United States will be subject to foreign regulatory requirements governing clinical trials and
marketing approval. Even if the FDA grants marketing approval for a product candidate, comparable foreign regulatory
authorities also must approve the manufacturing and marketing of the product candidate in those countries. Approval
procedures vary among jurisdictions and can involve requirements and administrative review periods different from, and
more onerous than, those in the United States, including additional preclinical studies or clinical trials. In many countries
outside the United States, a product candidate must be approved for reimbursement before it can be approved for sale in
that country. In some cases, the price that we intend to charge for any product candidates, if approved, is also subject to
approval. Obtaining approval for our product candidates in the European Union from the European Commission following
the opinion of the European Medicines Agency, or the EMA, if we choose to submit a marketing authorization application
there, would be a lengthy and expensive process. Even if a product candidate is approved, the EMA may limit the
indications for which the drug may be marketed, require extensive warnings on the drug labeling or require expensive and
time-consuming additional clinical trials or reporting as conditions of approval. Obtaining foreign regulatory approvals and
compliance with foreign regulatory requirements could result in significant delays, difficulties and costs for us and could
delay or prevent the introduction of our product candidates in certain countries.

Further, clinical trials conducted in one country may not be accepted by regulatory authorities in other countries.

Also, regulatory approval for our product candidates may be withdrawn. If we fail to comply with the applicable regulatory
requirements, our target market will be reduced and our ability to realize the full market potential of our product candidates
will be harmed and our business, financial condition, results of operations and prospects could be harmed.

If we commercialize our product candidates outside the United States, a variety of risks associated with

international operations could harm our business.

We intend to seek approval to market our product candidates outside the United States, and may do so for future

product candidates. If we market approved products outside the United States, we expect that we will be subject to
additional risks in commercialization, including:

● different regulatory requirements for approval of therapies in foreign countries;
● reduced protection for intellectual property rights;
● unexpected changes in tariffs, trade barriers and regulatory requirements;
● economic weakness, including inflation, or political instability in particular foreign economies and markets;
● compliance with tax, employment, immigration and labor laws for employees living or traveling abroad;
● foreign currency fluctuations, which could result in increased operating expenses and reduced revenues, and

other obligations incident to doing business in another country;

● foreign reimbursement, pricing and insurance regimes;
● workforce uncertainty in countries where labor unrest is more common than in the United States;
● production shortages resulting from any events affecting raw material supply or manufacturing capabilities

abroad; and

● business interruptions resulting from geopolitical actions, including war and terrorism, international

hostilities, or natural disasters including earthquakes, typhoons, floods and fires.

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We have no prior experience in these areas. In addition, there are complex regulatory, tax, labor and other legal
requirements imposed by many of the individual countries in which we may operate, with which we will need to comply.
Many biopharmaceutical companies have found the process of marketing their products in foreign countries to be
challenging.

Product liability lawsuits against us could cause us to incur substantial liabilities and could limit

commercialization of any product candidate that we may develop.

We face an inherent risk of product liability exposure related to the testing of our product candidates in clinical

trials and may face an even greater risk if we commercialize any product candidate that we may develop. If we cannot
successfully defend ourselves against claims that any such product candidates caused injuries, we could incur substantial
liabilities. Regardless of merit or eventual outcome, liability claims may result in:

● decreased demand for any product candidate that we may develop;
● loss of revenue;
● substantial monetary awards to trial participants or patients;
● significant time and costs to defend the related litigation;
● withdrawal of clinical trial participants;
● increased insurance costs;
● the inability to commercialize any product candidate that we may develop; and
● injury to our reputation and significant negative media attention.

Any such outcomes could negatively impact our business, financial condition, results of operations and prospects.

Our insurance policies may be inadequate and potentially expose us to unrecoverable risks.

Although we maintain product liability insurance coverage, such insurance may not be adequate to cover all

liabilities that we may incur. We anticipate that we will need to increase our insurance coverage each time we commence a
clinical trial and if we successfully commercialize any product candidate. Insurance availability, coverage terms and
pricing continue to vary with market conditions. We endeavor to obtain appropriate insurance coverage for insurable risks
that we identify; however, we may fail to correctly anticipate or quantify insurable risks, we may not be able to obtain
appropriate insurance coverage and insurers may not respond as we intend to cover insurable events that may occur. We
have observed rapidly changing conditions in the insurance markets relating to nearly all areas of traditional corporate
insurance. Such conditions have resulted in higher premium costs, higher policy deductibles, and lower coverage limits.
For some risks, we may not have or maintain insurance coverage because of cost or availability.

Risks Related to Regulatory Compliance

Our relationships with customers, physicians, and third party payors are subject, directly or indirectly, to

federal and state healthcare fraud and abuse laws, false claims laws, health information privacy and security laws, and
other healthcare laws and regulations. If we are unable to comply, or have not fully complied, with such laws, we could
face substantial penalties.

Healthcare providers, physicians and third-party payors in the United States and elsewhere will play a primary

role in the recommendation and prescription of any product candidates for which we obtain marketing approval. Our
current and future arrangements with healthcare professionals, principal investigators, consultants, customers and third-
party payors subject us to various federal and state fraud and abuse laws and other healthcare laws, including, without
limitation, the federal Anti-Kickback Statute, the federal civil and criminal false claims laws and the law commonly
referred to as the Physician Payments Sunshine Act and regulations.

Ensuring that our business arrangements with third-parties comply with applicable healthcare laws and regulations

will likely be costly. It is possible that governmental authorities will conclude that our business practices

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may not comply with current or future statutes, regulations or case law involving applicable fraud and abuse or other
healthcare laws and regulations. If our operations are found to be in violation of any of these laws or any other
governmental regulations that may apply to us, we may be subject to significant civil, criminal and administrative
penalties, damages, fines, disgorgement, imprisonment, exclusion from participating in government-funded healthcare
programs, such as Medicare and Medicaid, additional reporting requirements and oversight if we become subject to a
corporate integrity agreement or similar agreement to resolve allegations of noncompliance with these laws, contractual
damages, reputational harm and the curtailment or restructuring of our operations.

If the physicians or other providers or entities with whom we expect to do business are found not to be in

compliance with applicable laws, they may be subject to criminal, civil or administrative sanctions, including exclusions
from government-funded healthcare programs. Even if resolved in our favor, litigation or other legal proceedings relating
to healthcare laws and regulations may cause us to incur significant expenses and could distract our technical and
management personnel from their normal responsibilities. In addition, there could be public announcements of the results
of hearings, motions or other interim proceedings or developments. If securities analysts or investors perceive these results
to be negative, it could have a substantial adverse effect on the price of our common shares. Such litigation or proceedings
could substantially increase our operating losses and reduce the resources available for development, manufacturing, sales,
marketing or distribution activities. Uncertainties resulting from the initiation and continuation of litigation or other
proceedings relating to applicable healthcare laws and regulations could have an adverse effect on our ability to compete in
the marketplace.

Coverage and adequate reimbursement may not be available for our product candidates, which could make it

difficult for us to sell profitably, if approved.

Market acceptance and sales of any product candidates that we commercialize, if approved, will depend in part on

the extent to which reimbursement for these drugs and related treatments will be available from third-party payors,
including government health administration authorities, managed care organizations and other private health insurers.
Third-party payors decide which therapies they will pay for and establish reimbursement levels. While no uniform policy
for coverage and reimbursement exists in the United States, third-party payors often rely upon Medicare coverage policy
and payment limitations in setting their own coverage and reimbursement policies. However, decisions regarding the extent
of coverage and amount of reimbursement to be provided for any product candidates that we develop will be made on a
payor-by-payor basis. Therefore, one payor’s determination to provide coverage for a drug does not assure that other
payors will also provide coverage, and adequate reimbursement, for the drug. Additionally, a third-party payor’s decision
to provide coverage for a therapy does not imply that an adequate reimbursement rate will be approved. Each payor
determines whether or not it will provide coverage for a therapy, what amount it will pay the manufacturer for the therapy,
and on what tier of its formulary it will be placed. The position on a payor’s list of covered drugs, or formulary, generally
determines the co-payment that a patient will need to make to obtain the therapy and can strongly influence the adoption of
such therapy by patients and physicians. Patients who are prescribed treatments for their conditions and providers
prescribing such services generally rely on third-party payors to reimburse all or part of the associated healthcare costs.
Patients are unlikely to use our product candidates, if approved, unless coverage is provided and reimbursement is adequate
to cover a significant portion of the cost of our products.

Third-party payors have attempted to control costs by limiting coverage and the amount of reimbursement for

particular medications. We cannot be sure that coverage and reimbursement will be available for any drug that we
commercialize and, if reimbursement is available, what the level of reimbursement will be. Inadequate coverage and
reimbursement may impact the demand for, or the price of, any drug for which we obtain marketing approval. If coverage
and adequate reimbursement are not available, or are available only at limited levels, we may not be able to successfully
commercialize any product candidates that we develop.

Healthcare reform measures may have a negative impact on our business and results of operations.

In the United States and some foreign jurisdictions, there have been, and continue to be, several legislative and

regulatory changes and proposed changes, as well as judicial challenges, regarding the healthcare system that could prevent
or delay marketing approval of product candidates, restrict or regulate post-approval activities, and affect our ability to
profitably sell any product candidates for which we obtain marketing approval. In particular, there have been

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and continue to be a number of initiatives at the U.S. federal and state levels that seek to reduce healthcare costs and
improve the quality of healthcare. For example, the Medicare Prescription Drug, Improvement, and Modernization Act of
2003, or the MMA, changed the way Medicare covers and pays for pharmaceutical products. The legislation expanded
Medicare coverage for drug purchases by the elderly and introduced a new reimbursement methodology based on average
sales prices for physician-administered drugs. In addition, this legislation provided authority for limiting the number of
drugs that will be covered in any therapeutic class. Cost reduction initiatives and other provisions of this legislation could
decrease the coverage and price that we receive for any approved products. While the MMA applies only to drug benefits
for Medicare beneficiaries, private payors often follow Medicare coverage policy and payment limitations in setting their
own reimbursement rates. Therefore, any reduction in reimbursement that results from the MMA may result in a similar
reduction in payments from private payors.

Further, in March 2010, the Patient Protection and Affordable Care Act of 2010, as amended by the Health Care
and Education Reconciliation Act of 2010, or, collectively, the PPACA, was passed, which substantially changed the way
healthcare is financed by both governmental and private payors in the United States. Some of the provisions of the PPACA
have yet to be fully implemented, while certain provisions have been subject to executive, judicial and Congressional
challenges. For example, the Tax Cuts and Jobs Act of 2017, or Tax Act includes a provision that repealed, effective
January 1, 2019, the tax-based shared responsibility payment imposed by the PPACA on certain individuals who fail to
maintain qualifying health coverage for all or part of a year, which is commonly referred to as the “individual mandate.”
Additionally, on January 22, 2018, then-President Trump signed a continuing resolution on appropriations for fiscal year
2018 that delayed the implementation of certain PPACA-mandated fees, including the so-called “Cadillac” tax on certain
high-cost employer-sponsored insurance plans, the annual fee imposed on certain health insurance providers based on
market share, and the medical device excise tax on non-exempt medical devices. Further, the Bipartisan Budget Act of
2018, or the BBA, among other things, amended the PPACA, effective January 1, 2019, to close the coverage gap in most
Medicare drug plans, commonly referred to as the “donut hole.” In July 2018, CMS published a final rule permitting
further collections and payments to and from certain PPACA-qualified health plans and health insurance issuers under the
PPACA adjustment program in response to the outcome of federal district court litigation regarding the method CMS uses
to determine this risk adjustment. On December 14, 2018, a U.S. District Court Judge in the Northern District of Texas, or
Texas District Court Judge, ruled that the individual mandate was a critical and inseverable feature of the PPACA, and
therefore, because it was repealed as part of the Tax Act, the remaining provisions of the PPACA were invalid as well. In
December 2019, the U.S. Court of Appeals for the Fifth Circuit upheld the lower court decision, which was then appealed
to the U.S. Supreme Court. The U.S. Supreme Court heard arguments in the case in November 2020 and issued its decision
in June 2021, ruling that the plaintiffs lacked the standing to challenge the individual mandate provision. In so holding, the
Supreme Court did not consider larger constitutional questions about the validity of this provision or the validity of the
PPACA in its entirety. Another case challenging the PPACA’s requirement that insurers cover certain preventative services
is currently pending before the same U.S. District Court Judge in the Northern District of Texas who ruled against the
individual mandate in 2018. In September 2022, the judge held that certain preventative services violated the U.S.
Constitution and set a schedule for additional briefing that will expand into January 2023. It is unclear how this or any
potential future litigation and other efforts to repeal and replace the PPACA will impact the PPACA. Congress may
consider additional legislation to repeal or repeal and replace other elements of the PPACA. We continue to evaluate the
effect that the PPACA and its possible repeal and replacement may have on our business and the potential profitability of
our product candidates.

Other legislative changes have been proposed and adopted since the PPACA was enacted. These changes include
aggregate reductions to Medicare payments to providers of 2% per fiscal year pursuant to the Budget Control Act of 2011,
which began in 2013, and due to subsequent legislative amendments to the statute, including the BBA, which will remain
in effect through 2027 unless additional Congressional action is taken. The American Taxpayer Relief Act of 2012, among
other things, further reduced Medicare payments to several providers, including hospitals and cancer treatment centers, and
increased the statute of limitations period for the government to recover overpayments to providers from three to
five years.

Additional changes that may affect our business include the expansion of programs such as Medicare payment for
performance initiatives for physicians under the Medicare Access and CHIP Reauthorization Act of 2015. At this time, the
full impact of the introduction of the Medicare quality payment program on overall physician reimbursement is unclear.

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Further, in the United States there has been heightened governmental scrutiny over the manner in which
manufacturers set prices for their marketed products, which has resulted in several Congressional inquiries and proposed
and enacted federal and state legislation designed to, among other things, bring more transparency to drug pricing, reduce
the cost of prescription drugs under government payor programs, and review the relationship between pricing and
manufacturer patient programs. While some of the proposed measures will require authorization through additional
legislation to become effective, the U.S. Congress have indicated that they will continue to seek new legislative and/or
administrative measures to control drug costs. For example, the Inflation Reduction Act of 2022 also seeks to reduce
prescription drug costs by, among other provisions, allowing Medicare to negotiate prices for certain high-cost prescription
drugs in Medicare Parts B and D, imposing an excise tax on pharmaceutical manufacturers that refuse to negotiate pricing
with Medicare, requiring inflation rebates to limit annual drug price increases in Medicare, redesigning the Medicare Part
D formula, and limiting cost-sharing for insulin products. It is unclear whether additional drug pricing and other healthcare
reform measures will be enacted, and if enacted, what effect they would have on our business. We expect that additional
U.S. federal healthcare reform measures will be adopted in the future, any of which could limit the amounts that the U.S.
federal government will pay for healthcare products and services, which could result in reduced demand for our current or
any future product candidates or additional pricing pressures. We cannot predict the likelihood, nature or extent of
government regulation that may arise from future legislation or administrative action in the United States or any other
jurisdiction. If we or any third parties we may engage are slow or unable to adapt to changes in existing or new
requirements or policies, or if we or such third parties are not able to maintain regulatory compliance, our current or any
future product candidates we may develop may lose any regulatory approval that may have been obtained and we may not
achieve or sustain profitability.

Further, on May 30, 2018, the Trickett Wendler, Frank Mongiello, Jordan McLinn, and Matthew Bellina Right to
Try Act of 2017, or the Right to Try Act, was signed into law. The law, among other things, provides a federal framework
for certain patients to access certain investigational new drug products that have completed a Phase 1 clinical trial and that
are undergoing investigation for FDA approval. Under certain circumstances, eligible patients can seek treatment without
enrolling in clinical trials and without obtaining FDA permission under the FDA expanded access program. There is no
obligation for a pharmaceutical manufacturer to make its drug products available to eligible patients as a result of the Right
to Try Act.

We expect that these and other healthcare reform measures that may be adopted in the future may result in more
rigorous coverage criteria and in additional downward pressure on the price that we receive for any approved drug, which
could have an adverse effect on demand for our product candidates if they are approved. Any reduction in reimbursement
from Medicare or other government programs may result in a similar reduction in payments from private payors. The
implementation of cost containment measures or other healthcare reforms may prevent us from being able to generate
revenue, attain profitability or commercialize our product candidates.

Risks Related to Our Dependence on Third Parties

We intend to rely on third parties to produce clinical and commercial supplies of our product candidates.

We do not own or operate facilities for drug manufacturing, storage and distribution, or testing. We are dependent
on third parties to manufacture the clinical supplies of our current and any future product candidates. The facilities used by
our contract manufacturers to manufacture our product candidates must be approved by the FDA pursuant to inspections
that will be conducted after we submit our NDA to the FDA. We do not control the manufacturing process of, and are
completely dependent on, our contract manufacturing partners for compliance with the cGMP requirements, for
manufacture of both active drug substance and finished drug product. If our contract manufacturers cannot successfully
manufacture material that conforms to our specifications and the strict regulatory requirements of the FDA or others, we
will not be able to secure and/or maintain regulatory approval for our product candidates. In addition, we have no control
over the ability of our contract manufacturers to maintain adequate quality control, quality assurance and qualified
personnel. If the FDA or a comparable foreign regulatory authority does not approve these facilities for the manufacture of
our product candidates or if it withdraws any such approval in the future, we may need to find alternative manufacturing
facilities, which would significantly impact our ability to develop, obtain regulatory approval for or market our product
candidates, if approved. Any significant delay in the supply of a product candidate, or the raw material components thereof,
for an ongoing clinical trial due to the need to replace a third-party

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manufacturer could considerably delay completion of our clinical trials, product testing and potential regulatory approval
of our product candidates.

We also intend to rely on third-party manufacturers to supply us with sufficient quantities of our product
candidates to be used, if approved, for commercialization. We do not yet have a commercial supply agreement for
commercial quantities of drug substance or drug product. If we are not able to meet market demand for any approved
product, it would negatively impact our ability to generate revenue, harm our reputation, and could have an adverse effect
on our business and financial condition.

Further, our reliance on third-party manufacturers entails risks to which we would not be subject if we

manufactured product candidates ourselves, including:

● inability to meet our product specifications and quality requirements consistently;
● delay or inability to procure or expand sufficient manufacturing capacity;
● issues related to scale-up of manufacturing;
● costs and validation of new equipment and facilities required for scale-up;
● our third party manufacturers may not be able to execute our manufacturing procedures and other logistical

support requirements appropriately;

● our third party manufacturers may fail to comply with cGMP requirements and other inspections by the FDA

or other comparable regulatory authorities;

● our inability to negotiate manufacturing agreements with third parties under commercially reasonable terms,

if at all;

● breach, termination or nonrenewal of manufacturing agreements with third parties in a manner or at a time

that is costly or damaging to us;

● reliance on single sources for drug components;
● lack of qualified backup suppliers for those components that are currently purchased from a sole or single-

source supplier;

● our third party manufacturers may not devote sufficient resources to our product candidates;
● we may not own, or may have to share, the intellectual property rights to any improvements made by our

third party manufacturers in the manufacturing process for our product candidates;

● operations of our third party manufacturers or suppliers could be disrupted by conditions unrelated to our

business or operations, including the bankruptcy of the manufacturer or supplier; and

● carrier disruptions or increased costs that are beyond our control.

In addition, if we enter into a strategic collaboration with a third party for the commercialization of our current or

any future product candidates, we will not be able to control the amount of time or resources that they devote to such
efforts. If any strategic collaborator does not commit adequate resources to the marketing and distribution of our product
candidates, it could limit our potential revenues.

Any of these events could lead to clinical trial delays or failure to obtain regulatory approval, or impact our ability

to successfully commercialize our current or any future product candidates once approved. Some of these events could be
the basis for FDA action, including injunction, request for recall, seizure, or total or partial suspension of production.

Our business involves the use of hazardous materials and we and our third-party manufacturers and suppliers

must comply with environmental, health and safety laws and regulations, which can be expensive and restrict how we
do, or interrupt our, business.

Our research and development activities and our third-party manufacturers’ and suppliers’ activities involve the

generation, storage, use and disposal of hazardous materials, including the components of our product candidates and other
hazardous compounds and wastes. We and our manufacturers and suppliers are subject to environmental, health and safety
laws and regulations governing, among other matters, the use, manufacture, generation, storage, handling, transportation,
discharge and disposal of these hazardous materials and wastes and worker health and safety. In some

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cases, these hazardous materials and various wastes resulting from their use are stored at our and our manufacturers’
facilities pending their use and disposal. We cannot eliminate the risk of contamination or injury, which could result in an
interruption of our commercialization efforts, research and development efforts and business operations, damages and
significant cleanup costs and liabilities under applicable environmental, health and safety laws and regulations. We also
cannot guarantee that the safety procedures utilized by our third-party manufacturers for handling and disposing of these
materials and wastes generally comply with the standards prescribed by these laws and regulations. We may be held liable
for any resulting damages, costs or liabilities, which could exceed our resources, and state or federal or other applicable
authorities may curtail our use of certain materials and/or interrupt our business operations. Furthermore, environmental,
health and safety laws and regulations are complex, change frequently and have tended to become more stringent. We
cannot predict the impact of such changes and cannot be certain of our future compliance. Failure to comply with these
environmental, health and safety laws and regulations may result in substantial fines, penalties or other sanctions. We do
not currently carry environmental insurance coverage.

We rely on third-parties to conduct, supervise and monitor our preclinical studies and clinical trials, and if

those third parties perform in an unsatisfactory manner, it may harm our business.

We do not currently have the ability to independently conduct any clinical trials. We intend to rely on CROs and

clinical trial sites to ensure the proper and timely conduct of our preclinical studies and clinical trials, and we expect to
have limited influence over their actual performance. We rely upon CROs to monitor and manage data for our clinical
programs, as well as the execution of future preclinical studies. We expect to control only certain aspects of our CROs’
activities. Nevertheless, we will be responsible for ensuring that each of our preclinical studies and clinical trials is
conducted in accordance with the applicable protocol, legal, regulatory and scientific standards, and our reliance on the
CROs does not relieve us of our regulatory responsibilities.

We and our CROs are required to comply with the good laboratory practices, or GLPs, and GCPs, which are

regulations and guidelines enforced by the FDA and comparable foreign regulatory authorities in the form of International
Conference on Harmonization guidelines for any of our product candidates that are in preclinical and clinical development.
The regulatory authorities enforce GCPs through periodic inspections of trial sponsors, principal investigators and clinical
trial sites. Although we rely on CROs to conduct GCP-compliant clinical trials, we remain responsible for ensuring that
each of our GLP preclinical studies and clinical trials is conducted in accordance with its investigational plan and protocol
and applicable laws and regulations. If we or our CROs fail to comply with GCPs, the clinical data generated in our clinical
trials may be deemed unreliable, and the FDA or comparable foreign regulatory authorities may require us to perform
additional clinical trials before approving our marketing applications. Accordingly, if our CROs fail to comply with these
regulations or fail to recruit a sufficient number of subjects, we may be required to repeat clinical trials, which would delay
the regulatory approval process.

Our reliance on third parties to conduct clinical trials will result in less direct control over the management of data

developed through clinical trials than would be the case if we were relying entirely upon our own staff. Communicating
with CROs and other third parties can be challenging, potentially leading to mistakes as well as difficulties in coordinating
activities. Such parties may:

● have staffing difficulties;
● fail to comply with contractual obligations;
● experience regulatory compliance issues; or
● undergo changes in priorities or become financially distressed.

These factors may adversely affect the willingness or ability of third parties to conduct our clinical trials and may

subject us to unexpected cost increases that are beyond our control. If our CROs do not successfully carry out their
contractual duties or obligations, fail to meet expected deadlines, or fail to comply with regulatory requirements, or if the
quality or accuracy of the clinical data they obtain is compromised due to the failure to adhere to our clinical protocols or
regulatory requirements or for any other reasons, our clinical trials may be extended, delayed or terminated, and we may
not be able to obtain regulatory approval for, or successfully commercialize, any product candidate that we develop. As a
result, our financial results and the commercial prospects for any product candidate that we develop would be harmed, our
costs could increase, and our ability to generate revenue could be delayed. While we will have agreements governing

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their activities, our CROs will not be our employees, and we will not control whether or not they devote sufficient time and
resources to our future clinical and preclinical programs. These CROs may also have relationships with other commercial
entities, including our competitors, for whom they may also be conducting clinical trials, or other drug development
activities which could harm our business. We face the risk of potential unauthorized disclosure or misappropriation of our
intellectual property by CROs, which may reduce our trade secret protection and allow our potential competitors to access
and exploit our proprietary technology.

If our relationship with any of these CROs terminates, we may not be able to enter into arrangements with

alternative CROs or do so on commercially reasonable terms. Switching or adding additional CROs involves substantial
cost and requires management time and focus. In addition, there is a natural transition period when a new CRO commences
work. As a result, delays occur, which can negatively impact our ability to meet our desired clinical development timelines.
While we intend to carefully manage our relationships with our CROs, there can be no assurance that we will not encounter
challenges or delays in the future or that these delays or challenges will not have a negative impact on our business,
financial condition and prospects.

In addition, principal investigators for our clinical trials may serve as scientific advisors or consultants to us from
time to time and receive compensation in connection with such services. Under certain circumstances, we may be required
to report some of these relationships to the FDA. The FDA may conclude that a financial relationship between us and a
principal investigator has created a conflict of interest or otherwise affected interpretation of the trial. The FDA may
therefore question the integrity of the data generated at the applicable clinical trial site and the utility of the clinical trial
itself may be jeopardized. This could result in a delay in approval, or rejection, of our marketing applications by the FDA
and may ultimately lead to the denial of marketing approval of our product candidates.

Risks Related to Our Intellectual Property

Licensing of intellectual property is of critical importance to our business and involves complex legal, business

and scientific issues. If we breach our license agreements with Columbia University or any of the other agreements
under which we acquired, or will acquire, the intellectual property rights to our product candidates, we could lose the
ability to continue the development and commercialization of the related product.

The licensing of intellectual property is of critical importance to our business and to our current and future product

candidates, and we expect to enter into additional such agreements in the future. In particular, our current product
candidates AT-007, AT-001 and AT-003 are dependent on our license agreement with The Trustees of Columbia University
in the City of New York, or Columbia University. Pursuant to that license agreement with Columbia University, or the 2016
Columbia Agreement, Columbia University granted us an exclusive license under two important patent families, and a
nonexclusive license to certain know-how, owned by Columbia University to develop, manufacture or commercialize
certain compounds, including AT-001, AT-003 and AT-007, for the diagnosis and treatment of human and animal diseases
and conditions. The license grant is worldwide, with the exception of the patent family that covers AT-001 and AT-003. The
license grant for the patent family that covers AT-001 and AT-003 excludes patent rights in China, Taiwan, Hong Kong and
Macao, which Columbia University has exclusively licensed to a third party. We cannot prevent Columbia University’s
third party licensee from developing, manufacturing or commercializing certain compounds, including AT-001 and AT-003,
but not including AT-007, in China, Taiwan, Hong Kong and Macao, and we cannot develop, manufacture or
commercialize AT-001 or AT-003 in these territories, which could have a negative effect on our business.

We do not have the right to control the preparation, filing, prosecution and maintenance of patents and patent
applications covering the technology that we license under either of the Columbia Agreements. Therefore, we cannot
always be certain that these patents and patent applications will be prepared, filed, prosecuted and maintained in a manner
consistent with the best interests of our business. Although we have a right to have our comments considered in connection
with the prosecution process, if Columbia University fails to prosecute and maintain such patents, or loses rights to those
patents or patent applications as a result of its control of the prosecution activities, the rights we have licensed may be
reduced or eliminated, and our right to develop and commercialize any of our product candidates that are the subject of
such licensed rights could be adversely affected.

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If we fail to meet our obligations under the Columbia Agreement in any material respect and fail to cure such

breach in a timely fashion, then Columbia University may terminate the Columbia Agreement. If the Columbia Agreement
is terminated, and we lose our intellectual property rights under the Columbia Agreement, this may result in complete
termination of our product development and any commercialization efforts for the product candidates that are subject to the
agreement, including AT-007, AT-001, and AT-003. While we would expect to exercise all rights and remedies available to
us, including seeking to cure any breach by us, and otherwise seek to preserve our rights under the Columbia Agreement,
we may not be able to do so in a timely manner, at an acceptable cost or at all.

Furthermore, license agreements we enter into in the future may not provide exclusive rights to use intellectual

property and technology in all relevant fields of use and in all territories in which we may wish to develop or
commercialize our technology and products. As a result, we may not be able to prevent competitors from developing and
commercializing competitive products in territories included in all of our licenses.

If we are unable to obtain and maintain patent protection for our product candidates and technology, or if the

scope of the patent protection obtained is not sufficiently broad or robust, our competitors could develop and
commercialize products and technology similar or identical to ours, and our ability to successfully commercialize our
product candidates and technology may be adversely affected.

Our success depends, in large part, on our ability to obtain and maintain patent protection in the United States and
other countries with respect to our product candidates and our technology. We and our licensors have sought, and intend to
seek, to protect our proprietary position by filing patent applications in the United States and abroad related to our product
candidates and our technology that are important to our business.

The patent position of biotechnology and pharmaceutical companies generally is highly uncertain, involves

complex legal and factual questions and has, in recent years, been the subject of much litigation. As a result, the issuance,
scope, validity, enforceability and commercial value of our patent rights are highly uncertain. Our pending and future
patent applications may not result in patents being issued which protect our technology or product candidates or which
effectively prevent others from commercializing competitive technologies and product candidates. Since patent
applications in the United States and most other countries are confidential for a period of time after filing, and some remain
so until issued, we cannot be certain that we or our licensors were the first to file a patent application relating to any
particular aspect of a product candidate. Furthermore, if third parties have filed such patent applications, an interference
proceeding in the United States can be initiated by such third party, or by the U.S. Patent and Trademark Office, or
USPTO, itself, to determine who was the first to invent any of the subject matter covered by the patent claims of our
applications.

The patent prosecution process is expensive, time-consuming and complex, and we may not be able to file,

prosecute, maintain, enforce or license all necessary or desirable patent applications at a reasonable cost or in a timely
manner. It is also possible that we will fail to identify patentable aspects of our research and development output before it is
too late to obtain patent protection.

We or our licensors have not pursued or maintained, and may not pursue or maintain in the future, patent

protection for our product candidates in every country or territory in which we may sell our products, if approved. In
addition, the laws of some foreign countries do not protect intellectual property rights to the same extent as federal and
state laws in the United States. Consequently, we may not be able to prevent third parties from infringing our patents in all
countries outside the United States, or from selling or importing products that infringe our patents in and into the United
States or other jurisdictions.

Moreover, the coverage claimed in a patent application can be significantly reduced before the patent is issued,

and its scope can be reinterpreted after issuance. Even if the patent applications we license or own do issue as patents, they
may not issue in a form that will provide us with any meaningful protection, prevent competitors or other third parties from
competing with us or otherwise provide us with any competitive advantage. Our competitors or other third parties may be
able to circumvent our patents by developing similar or alternative products in a non-infringing manner.

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The issuance of a patent is not conclusive as to its inventorship, scope, validity or enforceability, and our patents

may be challenged in the courts or patent offices in the United States and abroad. Such challenges may result in loss of
exclusivity or in patent claims being narrowed, invalidated or held unenforceable, which could limit our ability to stop
others from using or commercializing similar or identical technology and products, or limit the duration of the patent
protection of our technology and product candidates. Given the amount of time required for the development, testing and
regulatory review of new product candidates, patents protecting such candidates might expire before or shortly after such
candidates are commercialized. As a result, our intellectual property may not provide us with sufficient rights to exclude
others from commercializing products similar or identical to ours.

Furthermore, our owned and in-licensed patents may be subject to a reservation of rights by one or more third

parties. For example, the research resulting in certain of our owned and in-licensed patent rights and technology was
funded in part by the U.S. government. As a result, the government may have certain rights, or march-in rights, to such
patent rights and technology. When new technologies are developed with government funding, the government generally
obtains certain rights in any resulting patents, including a nonexclusive license authorizing the government to use the
invention for noncommercial purposes. These rights may permit the government to disclose our confidential information to
third parties and to exercise march-in rights to use or allow third parties to use our licensed technology. The government
can exercise its march-in rights if it determines that action is necessary because we fail to achieve practical application of
the government-funded technology, because action is necessary to alleviate health or safety needs, to meet requirements of
federal regulations, or to give preference to U.S. industry. In addition, our rights in such inventions may be subject to
certain requirements to manufacture products embodying such inventions in the United States. Any exercise by the
government of such rights could harm our competitive position, business, financial condition, results of operations and
prospects.

Obtaining and maintaining our patent rights depends on compliance with various procedural, document

submission, fee payment and other requirements imposed by government patent agencies, and our patent protection
could be reduced or eliminated for noncompliance with these requirements.

The USPTO and various foreign governmental patent agencies require compliance with a number of procedural,

documentary, fee payment and other similar provisions during the patent application process. In addition, periodic
maintenance fees, renewal fees, annuity fees and various other government fees on patents and/or patent applications will
have to be paid to the USPTO and various government patent agencies outside the United States over the lifetime of our
owned and licensed patents and/or applications and any patent rights we may own or license in the future. We rely on our
service providers or our licensors to pay these fees. The USPTO and various non-U.S. government patent agencies require
compliance with several procedural, documentary, fee payment and other similar provisions during the patent application
process. We employ reputable law firms and other professionals to help us comply, and we are also dependent on our
licensors to take the necessary action to comply with these requirements with respect to our licensed intellectual property.
Noncompliance events that could result in abandonment or lapse of a patent or patent application include, but are not
limited to, failure to respond to official actions within prescribed time limits, nonpayment of fees and failure to properly
legalize and submit formal documents. If we or our licensors fail to maintain the patents and patent applications covering
our products or technologies, we may not be able to stop a competitor from marketing products that are the same as or
similar to our product candidates, which would have an adverse effect on our business. In many cases, an inadvertent lapse
can be cured by payment of a late fee or by other means in accordance with the applicable rules. There are situations,
however, in which noncompliance can result in abandonment or lapse of the patent or patent application, resulting in partial
or complete loss of patent rights in the relevant jurisdiction. In such an event, potential competitors might be able to enter
the market and this circumstance could harm our business.

In addition, if we fail to apply for applicable patent term extensions or adjustments, we will have a more limited
time during which we can enforce our granted patent rights. In addition, if we are responsible for patent prosecution and
maintenance of patent rights in-licensed to us, any of the foregoing could expose us to liability to the applicable patent
owner.

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Patent terms may be inadequate to protect our competitive position on our product candidates for an adequate

amount of time.

Given the amount of time required for the development, testing and regulatory review of product candidates such
as AT-007, AT-001, and AT-003, patents protecting such candidates might expire before or shortly after such candidates are
commercialized. We expect to seek extensions of patent terms in the United States and, if available, in other countries
where we have or will obtain patent rights. In the United States, the Drug Price Competition and Patent Term Restoration
Act of 1984 permits a patent term extension of up to five years beyond the normal expiration of the patent; provided that
the patent is not enforceable for more than 14 years from the date of drug approval, which is limited to the approved
indication (or any additional indications approved during the period of extension). Furthermore, only one patent per
approved product can be extended and only those claims covering the approved product, a method for using it or a method
for manufacturing it may be extended. However, the applicable authorities, including the FDA and the USPTO in the
United States, and any equivalent regulatory authority in other countries, may not agree with our assessment of whether
such extensions are available, and may refuse to grant extensions to our patents, or may grant more limited extensions than
we request. If this occurs, our competitors may be able to take advantage of our investment in development and clinical
trials by referencing our clinical and preclinical data and launch their drug earlier than might otherwise be the case.

Third-parties may initiate legal proceedings alleging that we are infringing, misappropriating or otherwise

violating their intellectual property rights, the outcome of which would be uncertain and could have a negative impact
on the success of our business.

Our commercial success depends, in part, upon our ability and the ability of others with whom we may collaborate

to develop, manufacture, market and sell our current and any future product candidates and use our proprietary
technologies without infringing, misappropriating or otherwise violating the proprietary rights and intellectual property of
third parties. The biotechnology and pharmaceutical industries are characterized by extensive and complex litigation
regarding patents and other intellectual property rights. We may in the future become party to, or be threatened with,
adversarial proceedings or litigation regarding intellectual property rights with respect to our current and any future product
candidates and technology, including interference proceedings, post grant review and inter partes review before the
USPTO. Third parties may assert infringement claims against us based on existing patents or patents that may be granted in
the future, regardless of their merit. There is a risk that third parties may choose to engage in litigation with us to enforce or
to otherwise assert their patent rights against us. Even if we believe such claims are without merit, a court of competent
jurisdiction could hold that these third-party patents are valid, enforceable and infringed, which could have a negative
impact on our ability to commercialize our current and any future product candidates. In order to successfully challenge the
validity of any such U.S. patent in federal court, we would need to overcome a presumption of validity. As this is a high
burden and requires us to present clear and convincing evidence as to the invalidity of any such U.S. patent claim, there is
no assurance that a court of competent jurisdiction would invalidate the claims of any such U.S. patent. Moreover, given
the vast number of patents in our field of technology, we cannot be certain that we do not infringe existing patents or that
we will not infringe patents that may be granted in the future. Other companies and research institutions have filed, and
may file in the future, patent applications related to AR inhibitors and their therapeutic use. Some of these patent
applications have already been allowed or issued, and others may issue in the future. While we may decide to initiate
proceedings to challenge the validity of these or other patents in the future, we may be unsuccessful, and courts or patent
offices in the United States and abroad could uphold the validity of any such patent. Furthermore, because patent
applications can take many years to issue and may be confidential for 18 months or more after filing, and because pending
patent claims can be revised before issuance, there may be applications now pending which may later result in issued
patents that may be infringed by the manufacture, use or sale of our product candidates. Regardless of when filed, we may
fail to identify relevant third-party patents or patent applications, or we may incorrectly conclude that a third-party patent is
invalid or not infringed by our product candidates or activities. If a patent holder believes that our product candidate
infringes its patent, the patent holder may sue us even if we have received patent protection for our technology. Moreover,
we may face patent infringement claims from nonpracticing entities that have no relevant drug revenue and against whom
our own patent portfolio may thus have no deterrent effect. If a patent infringement suit were threatened or brought against
us, we could be forced to stop or delay research, development, manufacturing or sales of the drug or product candidate that
is the subject of the actual or threatened suit.

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If we are found to infringe a third party’s valid and enforceable intellectual property rights, we could be required

to obtain a license from such third party to continue developing, manufacturing and marketing our product candidate(s) and
technology. Under any such license, we would most likely be required to pay various types of fees, milestones, royalties or
other amounts. Moreover, we may not be able to obtain any required license on commercially reasonable terms or at all.

The licensing or acquisition of third-party intellectual property rights is a competitive area, and more established

companies may also pursue strategies to license or acquire third-party intellectual property rights that we may consider
attractive or necessary. These established companies may have a competitive advantage over us due to their size, capital
resources and greater clinical development and commercialization capabilities. In addition, companies that perceive us to
be a competitor may be unwilling to assign or license rights to us. We also may be unable to license or acquire third-party
intellectual property rights on terms that would allow us to make an appropriate return on our investment or at all. If we are
unable to successfully obtain rights to required third-party intellectual property rights or maintain the existing intellectual
property rights we have, we may have to abandon development of the relevant program or product candidate, which could
have an adverse effect on our business, financial condition, results of operations and prospects. Furthermore, even if we
were able to obtain a license, it could be nonexclusive, thereby giving our competitors and other third-parties access to the
same technologies licensed to us, and it could require us to make substantial licensing and royalty payments. We could be
forced, including by court order, to cease developing, manufacturing and commercializing the infringing technology or
product candidate. In addition, we could be found liable for monetary damages, including treble damages and attorneys’
fees, if we are found to have willfully infringed a patent or other intellectual property right. We may be required to
indemnify collaborators or contractors against such claims. A finding of infringement could prevent us from manufacturing
and commercializing our current or any future product candidates or force us to cease some or all of our business
operations, which could harm our business. Even if we are successful in defending against such claims, litigation can be
expensive and time-consuming and would divert management’s attention from our core business. Furthermore, because of
the substantial amount of discovery required in connection with intellectual property litigation, there is a risk that some of
our confidential information could be compromised by disclosure during this type of litigation. There could also be public
announcements of the results of hearings, motions or other interim proceedings or developments. If securities analysts or
investors perceive these results to be negative, it could have an adverse effect on the price of our common stock.

Claims that we have misappropriated the confidential information or trade secrets of third parties could have a

similar negative impact on our business, financial condition, results of operations and prospects.

We may be subject to claims asserting that our employees, consultants or advisors have wrongfully used or

disclosed alleged trade secrets of their current or former employers or claims asserting ownership of what we regard as
our own intellectual property.

Certain of our employees, consultants or advisors are currently, or were previously, employed at universities or

other biotechnology or pharmaceutical companies, including our competitors or potential competitors. Although we try to
ensure that our employees, consultants and advisors do not use the proprietary information or know-how of others in their
work for us, we may be subject to claims that these individuals or we have used or disclosed intellectual property, including
trade secrets or other proprietary information, of any such individual’s current or former employer. Litigation may be
necessary to defend against these claims. If we fail in defending any such claims, in addition to paying monetary damages,
we may lose valuable intellectual property rights or personnel. Even if we are successful in defending against such claims,
litigation could result in substantial costs and be a distraction to management.

In addition, we may in the future be subject to claims by our former employees or consultants asserting an

ownership right in our patents or patent applications, as a result of the work they performed on our behalf. Although it is
our policy to require our employees and contractors who may be involved in the conception or development of intellectual
property to execute agreements assigning such intellectual property to us, we may be unsuccessful in executing such an
agreement with each party who, in fact, conceives or develops intellectual property that we regard as our own, and we
cannot be certain that our agreements with such parties will be upheld in the face of a potential challenge or that they will
not be breached, for which we may not have an adequate remedy. The assignment of intellectual property rights may not be
self-executing or the assignment agreements may be breached, and we may be

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forced to bring claims against third parties, or defend claims that they may bring against us, to determine the ownership of
what we regard as our intellectual property.

We may be involved in lawsuits to protect or enforce our patents, the patents of our licensors or our other

intellectual property rights, which could be expensive, time-consuming and unsuccessful.

Competitors may infringe, misappropriate or otherwise violate our patents, the patents of our licensors or our
other intellectual property rights. To counter infringement or unauthorized use, we may be required to file legal claims,
which can be expensive and time-consuming and are likely to divert significant resources from our core business, including
distracting our technical and management personnel from their normal responsibilities. In addition, in an infringement
proceeding, a court may decide that a patent of ours or our licensors is not valid or is unenforceable, or may refuse to stop
the other party from using the technology at issue on the grounds that our patents do not cover the technology in question.
An adverse result in any litigation or defense proceedings could put one or more of our owned or licensed patents at risk of
being invalidated or interpreted narrowly and could put our owned or licensed patent applications at risk of not issuing. The
initiation of a claim against a third party might also cause the third-party to bring counterclaims against us, such as claims
asserting that our patent rights are invalid or unenforceable. In patent litigation in the United States, defendant
counterclaims alleging invalidity or unenforceability are commonplace. Grounds for a validity challenge could be an
alleged failure to meet any of several statutory requirements, including lack of novelty, obviousness, non-enablement or
lack of statutory subject matter. Grounds for an unenforceability assertion could be an allegation that someone connected
with prosecution of the patent withheld relevant material information from the USPTO, or made a materially misleading
statement, during prosecution. Third parties may also raise similar validity claims before the USPTO in post-grant
proceedings such as ex parte reexaminations, inter partes review, post-grant review, or oppositions or similar proceedings
outside the United States, in parallel with litigation or even outside the context of litigation. The outcome following legal
assertions of invalidity and unenforceability is unpredictable. We cannot be certain that there is or will be no invalidating
prior art, of which we and the patent examiner were unaware during prosecution. For the patents and patent applications
that we have licensed, we may have limited or no right to participate in the defense of any licensed patents against
challenge by a third party. If a defendant were to prevail on a legal assertion of invalidity or unenforceability, we would
lose at least part, and perhaps all, of any future patent protection on our current or future product candidates. Such a loss of
patent protection could harm our business.

We may not be able to prevent, alone or with our licensors, misappropriation of our intellectual property rights,

particularly in countries where the laws may not protect those rights as fully as in the United States. Our business could be
harmed if in litigation the prevailing party does not offer us a license, or if the license offered as a result is not on
commercially reasonable terms. Any litigation or other proceedings to enforce our intellectual property rights may fail, and
even if successful, may result in substantial costs and distract our management and other employees.

Furthermore, because of the substantial amount of discovery required in connection with intellectual property

litigation, there is a risk that some of our confidential information could be compromised by disclosure during this type of
litigation. There could also be public announcements of the results of hearings, motions or other interim proceedings or
developments. If securities analysts or investors perceive these results to be negative, it could have an adverse effect on the
price of our common stock.

We may not have sufficient financial or other resources to adequately conduct such litigation or proceedings.

Some of our competitors may be able to sustain the costs of such litigation or proceedings more effectively than we can
because of their greater financial resources and more mature and developed intellectual property portfolios. Accordingly,
despite our efforts, we may not be able to prevent third parties from infringing upon or misappropriating or from
successfully challenging our intellectual property rights. Uncertainties resulting from the initiation and continuation of
patent litigation or other proceedings could have an adverse effect on our ability to compete in the marketplace.

Changes in U.S. patent law or the patent law of other countries or jurisdictions could diminish the value of

patents in general, thereby impairing our ability to protect our current and any future product candidates.

Changes in either the patent laws or interpretation of the patent laws in the United States could increase the
uncertainties and costs surrounding the prosecution of patent applications and the enforcement or defense of issued

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patents. Assuming that other requirements for patentability are met, prior to March 2013, in the United States, the first to
invent the claimed invention was entitled to the patent, while outside the United States, the first to file a patent application
was entitled to the patent. After March 2013, under the Leahy-Smith America Invents Act, or the America Invents Act, the
United States transitioned to a first inventor to file system in which, assuming that other requirements for patentability are
met, the first inventor to file a patent application will be entitled to the patent on an invention regardless of whether a third-
party was the first to invent the claimed invention. The America Invents Act also includes a number of significant changes
that affect the way patent applications are prosecuted and also may affect patent litigation. These include allowing third-
party submission of prior art to the USPTO during patent prosecution and additional procedures to attack the validity of a
patent by USPTO-administered post-grant proceedings, including post-grant review, inter partes review, and derivation
proceedings. However, the America Invents Act and its implementation could increase the uncertainties and costs
surrounding the prosecution of our patent applications and the enforcement or defense of our issued patents, all of which
could have an adverse effect on our business, financial condition, results of operations, and prospects.

In addition, the U.S. Supreme Court has ruled on several patent cases in recent years, either narrowing the scope

of patent protection available in certain circumstances or weakening the rights of patent owners in certain situations. In
addition to increasing uncertainty with regard to our ability to obtain patents in the future, this combination of events has
created uncertainty with respect to the value of patents, once obtained. Depending on actions by the U.S. Congress, the
federal courts, and the USPTO, the laws and regulations governing patents could change in unpredictable ways that could
weaken our ability to obtain new patents or to enforce patents that we own, have licensed or might obtain in the future.
Similarly, changes in patent law and regulations in other countries or jurisdictions, changes in the governmental bodies that
enforce them or changes in how the relevant governmental authority enforces patent laws or regulations may weaken our
ability to obtain new patents or to enforce patents that we own or have licensed or that we may obtain in the future.

We may not be able to protect our intellectual property rights throughout the world, which could negatively

impact our business.

Filing, prosecuting and defending patents covering our current and any future product candidates in all countries

throughout the world would be prohibitively expensive. Competitors may use our technologies in jurisdictions where we or
our licensors have not obtained patent protection to develop their own products and, further, may export otherwise
infringing products to territories where we may obtain patent protection but where patent enforcement is not as strong as
that in the United States. These products may compete with our products in jurisdictions where we do not have any issued
or licensed patents, and any future patent claims or other intellectual property rights may not be effective or sufficient to
prevent them from so competing.

Many companies have encountered significant problems in protecting and defending intellectual property rights in

foreign jurisdictions. The legal systems of certain countries, particularly certain developing countries, do not favor the
enforcement of patents, trade secrets and other intellectual property protection, particularly those relating to biotechnology
products, which could make it difficult for us to stop the infringement of our patents or marketing of competing products in
violation of our intellectual property and proprietary rights generally. Proceedings to enforce our intellectual property and
proprietary rights in foreign jurisdictions could result in substantial costs and divert our efforts and attention from other
aspects of our business, could put our patents at risk of being invalidated or interpreted narrowly, could put our patent
applications at risk of not issuing, and could provoke third parties to assert claims against us. We may not prevail in any
lawsuits that we initiate, and the damages or other remedies awarded, if any, may not be commercially meaningful.
Accordingly, our efforts to enforce our intellectual property and proprietary rights around the world may be inadequate to
obtain a significant commercial advantage from the intellectual property that we develop or license.

Many countries have compulsory licensing laws under which a patent owner may be compelled to grant licenses
to third parties. In addition, many countries limit the enforceability of patents against government agencies or government
contractors. In these countries, the patent owner may have limited remedies, which could materially diminish the value of
such patent. If we or any of our licensors is forced to grant a license to third parties with respect to

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any patents relevant to our business, our competitive position may be impaired, and our business, financial condition,
results of operations and prospects may be adversely affected.

Reliance on third parties requires us to share our trade secrets, which increases the possibility that a competitor

will discover them or that our trade secrets will be misappropriated or disclosed.

Since we rely on third parties to help us discover, develop and manufacture our current and any future product

candidates, or if we collaborate with third parties for the development, manufacturing or commercialization of our current
or any future product candidates, we must, at times, share trade secrets with them. We may also conduct joint research and
development programs that may require us to share trade secrets under the terms of our research and development
partnerships or similar agreements. We seek to protect our proprietary technology in part by entering into confidentiality
agreements and, if applicable, material transfer agreements, consulting agreements or other similar agreements with our
advisors, employees, third-party contractors and consultants prior to beginning research or disclosing proprietary
information. These agreements typically limit the rights of the third parties to use or disclose our confidential information,
including our trade secrets. Despite the contractual provisions employed when working with third parties, the need to share
trade secrets and other confidential information increases the risk that such trade secrets become known by our
competitors, are inadvertently incorporated into the technology of others, or are disclosed or used in violation of these
agreements. Given that our proprietary position is based, in part, on our know-how and trade secrets, a competitor’s
discovery of our trade secrets or other unauthorized use or disclosure could have an adverse effect on our business and
results of operations.

In addition, these agreements typically restrict the ability of our advisors, employees, third-party contractors and
consultants to publish data potentially relating to our trade secrets. Despite our efforts to protect our trade secrets, we may
not be able to prevent the unauthorized disclosure or use of our technical know-how or other trade secrets by the parties to
these agreements. Moreover, we cannot guarantee that we have entered into such agreements with each party that may have
or have had access to our confidential information or proprietary technology and processes. Monitoring unauthorized uses
and disclosures is difficult, and we do not know whether the steps we have taken to protect our proprietary technologies
will be effective. If any of the collaborators, scientific advisors, employees, contractors and consultants who are parties to
these agreements breaches or violates the terms of any of these agreements, we may not have adequate remedies for any
such breach or violation, and we could lose our trade secrets as a result. Moreover, if confidential information that is
licensed or disclosed to us by our partners, collaborators, or others is inadvertently disclosed or subject to a breach or
violation, we may be exposed to liability to the owner of that confidential information. Enforcing a claim that a third-party
illegally or unlawfully obtained and is using our trade secrets, like patent litigation, is expensive and time-consuming, and
the outcome is unpredictable. In addition, courts outside the United States are sometimes less willing to protect trade
secrets.

If we are unable to protect the confidentiality of our trade secrets, our business and competitive position would

be harmed.

In addition to seeking patent and trademark protection for our product candidates, we also rely on trade secrets,
including unpatented know-how, technology and other proprietary information, to maintain our competitive position. We
seek to protect our trade secrets, in part, by entering into nondisclosure and confidentiality agreements with parties who
have access to them, such as our employees, corporate collaborators, outside scientific collaborators, contract
manufacturers, consultants, advisors and other third parties. We also enter into confidentiality and invention or patent
assignment agreements with our employees, advisors and consultants. Despite these efforts, any of these parties may
breach the agreements and disclose our proprietary information, including our trade secrets. Monitoring unauthorized uses
and disclosures of our intellectual property is difficult, and we do not know whether the steps we have taken to protect our
intellectual property will be effective. In addition, we may not be able to obtain adequate remedies for any such breaches.
Enforcing a claim that a party illegally disclosed or misappropriated a trade secret is difficult, expensive and time-
consuming, and the outcome is unpredictable. In addition, some courts inside and outside the United States are less willing
or unwilling to protect trade secrets.

Moreover, our competitors may independently develop knowledge, methods and know-how equivalent to our

trade secrets. Competitors could purchase our products and replicate some or all of the competitive advantages we derive

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from our development efforts for technologies on which we do not have patent protection. If any of our trade secrets were
to be lawfully obtained or independently developed by a competitor, we would have no right to prevent them, or those to
whom they communicate it, from using that technology or information to compete with us. If any of our trade secrets were
to be disclosed to or independently developed by a competitor, our competitive position would be harmed.

We also seek to preserve the integrity and confidentiality of our data and other confidential information by
maintaining physical security of our premises and physical and electronic security of our information technology systems.
While we have confidence in these individuals, organizations and systems, agreements or security measures may be
breached, and detecting the disclosure or misappropriation of confidential information and enforcing a claim that a party
illegally disclosed or misappropriated confidential information is difficult, expensive and time-consuming, and the outcome
is unpredictable. Further, we may not be able to obtain adequate remedies for any breach. In addition, our confidential
information may otherwise become known or be independently discovered by competitors, in which case we would have
no right to prevent them, or those to whom they communicate it, from using that technology or information to compete
with us.

Any trademarks we may obtain may be infringed or successfully challenged, resulting in harm to our business.

We expect to rely on trademarks as one means to distinguish any of our product candidates that are approved for

marketing from the products of our competitors. We have selected trademarks for some of our later stage product
candidates and filed applications to register those trademarks for our current or any future product candidates. For other
earlier stage product candidates, we have not yet selected trademarks or begun the process of applying to register
trademarks. Our pending trademark applications, and any future trademark applications may not be approved. Third parties
may oppose our trademark applications or otherwise challenge our use of the trademarks. In the event that our trademarks
are successfully challenged, we could be forced to rebrand our products, which could result in loss of brand recognition
and could require us to devote resources to advertising and marketing new brands. Our competitors may infringe our
trademarks, and we may not have adequate resources to enforce our trademarks.

In addition, any proprietary name we propose to use with our current or any other product candidate in the United

States must be approved by the FDA, regardless of whether we have registered it, or applied to register it, as a trademark.
The FDA typically conducts a review of proposed product names, including an evaluation of the potential for confusion
with other product names. If the FDA objects to any of our proposed proprietary product names, we may be required to
expend significant additional resources in an effort to identify a suitable proprietary product name that would qualify under
applicable trademark laws, not infringe the existing rights of third parties and be acceptable to the FDA.

Intellectual property rights do not necessarily address all potential threats to our business.

The degree of future protection afforded by our intellectual property rights is uncertain because intellectual

property rights have limitations and may not adequately protect our business. The following examples are illustrative:

● others may be able to make compounds or formulations that are similar to our product candidates but that are

not covered by the claims of any patents, should they issue, that we own or license;

● we or our licensors might not have been the first to make the inventions covered by the issued patents or

pending patent applications that we own or license;

● we or our licensors might not have been the first to file patent applications covering certain of our inventions;
● others may independently develop similar or alternative technologies or duplicate any of our technologies

without infringing our intellectual property rights;

● it is possible that our pending patent applications will not lead to issued patents;
● issued patents that we own or license may not provide us with any competitive advantages, or may be held

invalid or unenforceable as a result of legal challenges;

● our competitors might conduct research and development activities in the United States and other countries
that provide a safe harbor from patent infringement claims for certain research and development activities,

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as well as in countries where we do not have patent rights, and then use the information learned from such
activities to develop competitive drugs for sale in our major commercial markets;

● we may not develop additional proprietary technologies that are patentable; and
● the patents of others may have an adverse effect on our business.

Risks Related to Our Business Operations, Employee Matters and Managing Growth

We are highly dependent on the services of our Chief Executive Officer and Chairman, Dr. Shoshana
Shendelman, and our Chief Medical Officer, Dr. Riccardo Perfetti, and if we are not able to retain these members of our
management team or recruit and retain additional management, clinical and scientific personnel, our business will be
harmed.

We are highly dependent on our Chief Executive Officer and Chairman, Dr. Shoshana Shendelman, and our Chief

Medical Officer, Dr. Riccardo Perfetti. Each of them may currently terminate their employment with us at any time. The
loss of the services of either of these persons could impede the achievement of our research, development and
commercialization objectives.

Recruiting and retaining other senior executives, qualified scientific and clinical personnel and, if we progress the
development of any of our product candidates, commercialization, manufacturing and sales and marketing personnel, will
be critical to our success. The loss of the services of our executive officers or other key employees could impede the
achievement of our research, development and commercialization objectives and seriously harm our ability to successfully
implement our business strategy. Furthermore, replacing executive officers and key employees may be difficult and may
take an extended period of time because of the limited number of individuals in our industry with the breadth of skills and
experience required to successfully develop, gain regulatory approval of and commercialize our product candidates.
Competition to hire from this limited pool is intense, and we may be unable to hire, train, retain or motivate these key
personnel on acceptable terms given the competition among numerous pharmaceutical and biotechnology companies for
similar personnel. We also experience competition for the hiring of scientific and clinical personnel from universities and
research institutions. In addition, we rely on consultants and advisors, including scientific and clinical advisors, to assist us
in formulating our research and development and commercialization strategy. Our consultants and advisors may have
commitments under consulting or advisory contracts with other entities that may limit their availability to us. If we are
unable to continue to attract and retain high-quality personnel, our ability to pursue our growth strategy will be limited.

Our future performance will also depend, in part, on our ability to successfully integrate newly hired executive

officers into our management team and our ability to develop an effective working relationship among senior management.
Our failure to integrate these individuals and create effective working relationships among them and other members of
management could result in inefficiencies in the development and commercialization of our product candidates, harming
future regulatory approvals, sales of our product candidates and our results of operations. Additionally, we do not currently
maintain “key person” life insurance on the lives of our executives or any of our employees.

We expect to expand our organization, and we may experience difficulties in managing this growth, which

could disrupt our operations.

As of December 31, 2022, we had 27 full-time employees. As the clinical development of our product candidates

progresses, we also expect to experience significant growth in the number of our employees and the scope of our
operations, particularly in the areas of research, drug development, regulatory affairs and, if any of our product candidates
receives marketing approval, sales, marketing and distribution. To manage our anticipated future growth, we must continue
to implement and improve our managerial, operational and financial systems, expand our facilities, and continue to recruit
and train additional qualified personnel. Due to our limited financial resources and the limited experience of our
management team in managing a company with such anticipated growth, we may not be able to effectively manage the
expansion of our operations or recruit and train additional qualified personnel. The expansion of our operations may lead to
significant costs and may divert our management and business development resources. Any inability to manage growth
could delay the execution of our business plans or disrupt our operations.

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Our internal computer systems, or those of our collaborators or other contractors or consultants, may fail or
suffer security breaches, which could result in a significant disruption of our product development programs and our
ability to operate our business effectively, and adversely affect our business and operating results.

Our internal computer systems, cloud-based computing services and those of our current and any future

collaborators and other contractors or consultants are vulnerable to damage or interruption from computer viruses, data
corruption, cyber-based attacks (including phishing attempts, denial of service attacks, and malware or ransomware
incidents), unauthorized access, natural disasters, terrorism, war, international hostilities and telecommunication and
electrical failures. While we have not experienced any significant system failure, accident or security breach to date, if such
an event were to occur and cause interruptions in our operations, it could result in a disruption of our development
programs and our business operations, whether due to a loss of our trade secrets or other proprietary information or other
similar disruptions. For example, the loss of clinical trial data from completed or future clinical trials could result in delays
in our regulatory approval efforts and significantly increase our costs to recover or reproduce the data. Furthermore,
federal, state and international laws and regulations, such as the European Union’s General Data Protection Regulation,
which took effect in May 2018, can expose us to enforcement actions and investigations by regulatory authorities, and
potentially result in regulatory penalties and significant legal liability, if our information technology security efforts fail. In
addition, our software systems include cloud-based applications that are hosted by third-party service providers with
security and information technology systems subject to similar risks. To the extent that any disruption or security breach
were to result in a loss of, or damage to, our data or applications, or inappropriate disclosure of confidential or proprietary
information, we could incur liability, our competitive position could be harmed and the further development and
commercialization of our product candidates could be delayed.

Risks of unauthorized access and cyber-attacks have increased as most of our personnel, and the personnel of
many third-parties with which we do business, have adopted remote working arrangements as a result of the Covid-19
pandemic, and may increase as a result of recent hostilities between Russia and Ukraine. Improper or inadvertent employee
behavior, including data privacy breaches by employees, contractors and others with permitted access to our systems, may
also pose a risk that sensitive data may be exposed to unauthorized persons or to the public. If a system failure or security
breach occurs and interrupts our operations or the operations at one of our third-party vendors, it could result in intellectual
property and other proprietary or confidential information being lost or stolen or a material disruption of our drug
development programs. For example, the loss of clinical trial data from ongoing or planned clinical trials could result in
delays in our regulatory approval efforts and significantly increase our costs to recover or reproduce the data. To the extent
that any disruption or security breach results in a loss of or damage to our data or applications, loss of trade secrets or
inappropriate disclosure of confidential or proprietary information, including protected health information or personal data
of employees or former employees, access to our clinical data, or disruption of the manufacturing process, we could incur
liability and the further development of our drug candidates could be delayed. We may also be vulnerable to cyber-attacks
by hackers or other malfeasance. This type of breach of our cybersecurity may compromise our confidential information
and/or our financial information and adversely affect our business or reputation or result in legal or regulatory proceedings.
In addition, if a ransomware attack or other cyber-attack occurs, either internally or at our third-party vendors, it is possible
we could be prevented from accessing our systems or data, which may cause interruptions or delays in our business, cause
us to incur remediation costs or subject us to demands to pay ransom, or adversely affect our business reputation.

Our employees, principal investigators, consultants and commercial partners may engage in misconduct or
other improper activities, including noncompliance with regulatory standards and requirements and insider trading.

We are exposed to the risk of fraud or other misconduct by our employees, principal investigators, consultants and
commercial partners. Misconduct by these parties could include intentional failures to comply with FDA regulations or the
regulations applicable in other jurisdictions, provide accurate information to the FDA and other regulatory authorities,
comply with healthcare fraud and abuse laws and regulations in the United States and abroad, report financial information
or data accurately or disclose unauthorized activities to us. In particular, sales, marketing and business arrangements in the
healthcare industry are subject to extensive laws and regulations intended to prevent fraud, misconduct, kickbacks, self-
dealing and other abusive practices. These laws and regulations restrict or prohibit a wide range of pricing, discounting,
marketing and promotion, sales commission, customer incentive programs, and other business arrangements. Such
misconduct also could involve the improper use of information obtained in the course of

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clinical trials or interactions with the FDA or other regulatory authorities, which could result in regulatory sanctions and
cause serious harm to our reputation. It is not always possible to identify and deter employee misconduct, and the
precautions we take to detect and prevent this activity may not be effective in controlling unknown or unmanaged risks or
losses or in protecting us from government investigations or other actions or lawsuits stemming from a failure to comply
with these laws or regulations. If any such actions are instituted against us and we are not successful in defending ourselves
or asserting our rights, those actions could result in significant civil, criminal and administrative penalties, damages, fines,
disgorgement, imprisonment, exclusion from participating in government-funded healthcare programs, such as Medicare
and Medicaid, additional reporting requirements and oversight if we become subject to a corporate integrity agreement or
similar agreement to resolve allegations of noncompliance with these laws, contractual damages, reputational harm and the
curtailment or restructuring of our operations, any of which could have a negative impact on our business, financial
condition, results of operations and prospects.

Any future acquisitions or strategic collaborations may increase our capital requirements, dilute our

stockholders, cause us to incur debt or assume contingent liabilities and/or subject us to other risks.

From time to time, we may evaluate various acquisitions and strategic collaborations, including licensing or

acquiring complementary drugs, intellectual property rights, technologies or businesses, as deemed appropriate to carry out
our business plan. Any potential acquisition or strategic partnership may entail numerous risks, including:

● increased operating expenses and cash requirements;
● the assumption of additional indebtedness or contingent or unknown liabilities;
● assimilation of operations, intellectual property and drugs of an acquired company, including difficulties

associated with integrating new personnel;

● the diversion of our management’s attention from our existing drug programs and initiatives in pursuing such

a strategic partnership, merger or acquisition;

● retention of key employees, the loss of key personnel, and uncertainties in our ability to maintain key

business relationships;

● risks and uncertainties associated with the other party to such a transaction, including the prospects of that

party and their existing drugs or product candidates and regulatory approvals; and

● our inability to generate revenue from acquired technology and/or drugs sufficient to meet our objectives in

undertaking the acquisition or even to offset the associated acquisition and maintenance costs.

In addition, if we engage in future acquisitions or strategic partnerships, we may issue dilutive securities, assume
or incur debt obligations, incur large one-time expenses, and acquire intangible assets that could result in significant future
amortization expense. Moreover, we may not be able to locate suitable acquisition opportunities, and this inability could
impair our ability to grow or obtain access to technology or drugs that may be important to the development of our
business.

Our business may be adversely affected by the coronavirus outbreak.

The Covid-19 pandemic, (“Covid-19”) has had and may continue to have a material impact on our operations.

Infections and deaths related to Covid-19 continue to disrupt the United States’ healthcare and healthcare regulatory
systems. Such disruptions could divert healthcare resources away from, or materially delay FDA approval with respect to,
our clinical trials. In addition, other known and unknown factors caused by Covid-19 could materially delay our clinical
trials, including our ability to recruit and retain patients and principal investigators and site staff who, as healthcare
providers, may have heightened exposure to Covid-19. For example, with respect to our trials related to AT-001 for the
treatment of Diabetic Cardiomyopathy, we have experienced, and may continue to experience, delays in patient enrollment.
Furthermore, we may experience additional delays in patient enrollment that we may not be able to mitigate. In addition,
we have partnered with clinical research organizations, or CROs, to conduct clinical studies in jurisdictions, such as the
EU, that have been affected by the spread of Covid-19. There is a possibility that such CROs may become unavailable or
that the clinical trials they manage may be delayed due to Covid-19 or containment efforts associated with it. Such events
may lead to termination of our relationship with affected CROs, affecting the development and study of our product
candidates. Any elongation or de-prioritization of our clinical trials or delay in regulatory review resulting from such
disruptions could materially affect the development and study of our product

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candidates, and increase the costs related to such development. While Covid-19 vaccines have become available both
domestically and internationally, the effects of Covid-19, including the impacts described above may last longer than
expected, extending such impacts, and materially impacting our business, financial condition, and results of operations. 

Risks Related to Ownership of Our Common Stock

The market price of our common stock is volatile and has fluctuated substantially, which could result in

substantial losses for purchasers of our common stock.

The stock market in general and the market for biopharmaceutical and pharmaceutical companies in particular, has

experienced extreme volatility that has often been unrelated to the operating performance of particular companies. As a
result of this volatility, you may not be able to sell your common stock at or above the price at which you purchased it. In
addition to the factors discussed in this “Risk Factors” section and elsewhere in this Annual Report, the market price for
our common stock has been, and is likely to continue to be influenced by the following:

● the commencement, enrollment, results of , or any delays in our planned or future clinical trials of our

product candidates or those of our competitors;

● the success of competitive drugs or therapies;
● regulatory or legal developments in the United States and other countries;
● the success of competitive products or technologies;
● developments or disputes concerning patent applications, issued patents or other proprietary rights;
● the recruitment or departure of key personnel;
● the level of expenses related to our product candidates or clinical development programs;
● the results of our efforts to discover, develop, acquire or in-license additional product candidates;
● actual or anticipated changes in estimates as to financial results, development timelines or recommendations

by securities analysts;

● our inability to obtain or delays in obtaining adequate drug supply for any approved drug or inability to do so

at acceptable prices;

● disputes or other developments relating to proprietary rights, including patents, litigation matters and our

ability to obtain patent protection for our technologies;

● the potential impact of the Covid-19 pandemic on the timing and progress of our ongoing clinical trials, our
business, results of operations, liquidity, and operations and our ability to mitigate those potential impacts;

● significant lawsuits, including patent or stockholder litigation;
● variations in our financial results or those of companies that are perceived to be similar to us;
● changes in the structure of healthcare payment systems, including coverage and adequate reimbursement for

any approved drug;

● market conditions in the pharmaceutical and biotechnology sectors;
● general economic, political, and market conditions and overall fluctuations in the financial markets in the

United States and abroad; and

● investors’ general perception of us and our business.

These and other market and industry factors have caused the market price and demand for our common stock to
fluctuate substantially, regardless of our actual operating performance, which may limit or prevent investors from selling
their shares at or above the price paid for the shares and may otherwise negatively affect the liquidity of our common stock.
Furthermore, we believe our stock has been, and may in the future be, adversely affected as a result of actions by third-
parties. Short sellers and others, some of whom post anonymously on social media, may be positioned to profit if our stock
declines and their activities can negatively affect our stock price.

Some companies that have experienced volatility in the trading price of their shares have been the subject of

securities class action litigation. Any lawsuit to which we are a party, with or without merit, may result in an unfavorable
judgment. We also may decide to settle lawsuits on unfavorable terms. Any such negative outcome could result in
payments of substantial damages or fines, damage to our reputation or adverse changes to our business practices.
Defending against litigation is costly and time-consuming, and could divert our management’s attention and our

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resources. Furthermore, during the course of litigation, there could be negative public announcements of the results of
hearings, motions or other interim proceedings or developments, which could have a negative effect on the market price of
our common stock.

Concentration of ownership of our common stock among our existing executive officers, directors and

principal stockholders may prevent new investors from influencing significant corporate decisions.

Based upon shares of our common stock outstanding as of December 31, 2022, our executive officers, directors
and stockholders who owned more than 10% of our outstanding common stock, in the aggregate, beneficially own shares
representing approximately 40.1% of our outstanding common stock. If our executive officers, directors and stockholders
who owned more than 10% of our outstanding common stock acted together, they may be able to significantly influence all
matters requiring stockholder approval, including the election and removal of directors and approval of any merger,
consolidation or sale of all or substantially all of our assets. The concentration of voting power and transfer restrictions
could delay or prevent an acquisition of our company on terms that other stockholders may desire or result in the
management of our company in ways with which other stockholders disagree.

Because we do not anticipate paying any cash dividends on our capital stock in the foreseeable future, capital

appreciation, if any, will be your sole source of gain.

You should not rely on an investment in our common stock to provide dividend income. We have never declared

or paid cash dividends on our capital stock. We currently intend to retain all of our future earnings, if any, to finance the
growth and development of our business. In addition, the terms of any future debt agreements may preclude us from paying
dividends. As a result, capital appreciation, if any, of our common stock will be your sole source of gain for the foreseeable
future. Investors seeking cash dividends should not purchase our common stock.

Future sales of common stock by holders of our common stock, or the perception that such sales may occur,

could depress the market price of our common stock.

Sales of a substantial number of shares of our common stock in the public market could occur at any time, subject
to certain restrictions described below. These sales, or the perception in the market that holders of a large number of shares
intend to sell shares, could reduce the market price of our common stock. As of December 31, 2022, we had outstanding
48,063,358 shares of common stock. A substantial number of such shares are currently restricted as a result of securities
laws or lock-up agreements but will be able to be sold in the future.

We further have registered all shares of common stock that we may issue in the future or have issued to date under

our equity compensation plans. These shares can be freely sold in the public market upon issuance, subject to volume
limitations applicable to affiliates and certain lock-up agreements. Sales of a large number of the shares issued under these
plans in the public market could have an adverse effect on the market price of our common stock.

If we fail to regain compliance with the continued listing requirements of Nasdaq, our common stock may be
delisted and the price of our common stock and our ability to access the capital markets could be negatively impacted. 

On November 15, 2022, we received a deficiency letter from the staff of the Listing Qualifications Department of
the Nasdaq Stock Market, or Nasdaq, notifying us that we were not in compliance with Listing Rule 5450(b)(1)(A), which
requires a minimum of $10 million in stockholders’ equity, for companies listed under the NASDAQ Global Market,
referred to as the equity rule. On February 24, 2023, the Nasdaq staff granted us an extension to regain compliance with the
equity rule, or to transition to the NASDAQ Capital Market, which has a lower stockholders’ equity requirement, by May
15, 2023. We intend to enter into one or more financing transactions in an effort to comply with the equity rule and may, if
appropriate, consider other available options.

There are many factors that may adversely affect our stockholders’ equity, including those described throughout

this section titled “Risk Factors.” Many of these factors are outside of our control. As a result, we may not be able to
regain, or once regained, sustain compliance with the equity rule or other Nasdaq rule market cap requirements in the

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long term. Any potential delisting of our common stock from the Nasdaq Global Market would likely result in decreased
liquidity and increased volatility for our common stock and would adversely affect our ability to raise additional capital or
to enter into strategic transactions. Any potential delisting of our common stock from the Nasdaq Global Market would
also make it more difficult for our stockholders to sell our common stock in the public market.

General Risk Factors

If research analysts do not publish research or reports, or publish unfavorable research or reports, about us,

our business or our market, our stock price and trading volume could decline.

The trading market for our common stock will be influenced by the research and reports that industry or financial

analysts publish about us or our business. Equity research analysts may discontinue research coverage of our common
stock, and such lack of research coverage may adversely affect the market price of our common stock. We do not have any
control over the analysts or the content and opinions included in their reports. The price of our shares could decline if one
or more equity research analysts downgrade our shares or issue other unfavorable commentary or research about us. If one
or more equity research analysts cease coverage of us or fail to publish reports on us regularly, demand for our shares could
decrease, which in turn could cause the trading price or trading volume of our common stock to decline.

We have broad discretion in the use of our cash and cash equivalents and may use them ineffectively, in ways

with which you do not agree or in ways that do not increase the value of your investment.

Our management has broad discretion in the application of our cash and cash equivalents, and could spend the

proceeds in ways that do not improve our results of operations or enhance the value of our common stock. The failure by
our management to apply these funds effectively could result in additional operating losses that could have a negative
impact on our business, cause the price of our common stock to decline and delay the development of our product
candidates. Pending their use, we may invest our cash and cash equivalents in a manner that does not produce income or
that loses value.

We are an “emerging growth company,” and the reduced disclosure requirements applicable to emerging

growth companies may make our common stock less attractive to investors.

We are an “emerging growth company,” or EGC, as defined in the Jumpstart Our Business Startups Act of 2012,

or the JOBS Act, and we intend to take advantage of some of the exemptions from reporting requirements that are
applicable to other public companies that are not EGCs, including:

● being permitted to provide only two years of audited financial statements, in addition to any required
unaudited interim financial statements, with correspondingly reduced “Management’s Discussion and
Analysis of Financial Condition and Results of Operations” disclosure;

● not being required to comply with the auditor attestation requirements in the assessment of our internal

control over financial reporting;

● not being required to comply with any requirement that may be adopted by the Public Company Accounting

Oversight Board regarding mandatory audit firm rotation or a supplement to the auditor’s report providing
additional information about the audit and the financial statements;
● reduced disclosure obligations regarding executive compensation; and
● not being required to hold a nonbinding advisory vote on executive compensation and stockholder approval

of any golden parachute payments not previously approved.

We cannot predict whether investors will find our common stock less attractive because we will rely on these

exemptions. If some investors find our common stock less attractive as a result, there may be a less active trading market
for our common stock and our share price may be more volatile. We currently take advantage of some or all of these
reporting exemptions until we are no longer an EGC. We will remain an EGC until the earlier of (i) December 31, 2024,
(ii) the last day of the fiscal year in which we have total annual gross revenue of at least $1.235 billion, (iii) the last day of
the first fiscal year in which we are deemed to be a large accelerated filer, which means the market value of our

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common stock that is held by non-affiliates exceeds $700 million as of the prior June 30th, and (iv) the date on which we
have issued more than $1.0 billion in non-convertible debt during the prior three-year period.

In addition, under Section 107(b) of the JOBS Act, EGCs can delay adopting new or revised accounting standards

until such time as those standards apply to private companies. We have irrevocably elected not to avail ourselves of this
exemption from new or revised accounting standards and, therefore, we will be subject to the same requirements to adopt
new or revised accounting standards as other public companies that are not EGCs.

We have incurred increased costs as a result of operating as a public company, and our management will be

required to devote substantial time to new compliance initiatives.

As a public company, and particularly after we are no longer an EGC, we incur and will continue to incur
significant legal, accounting and other expenses. In addition, the Sarbanes-Oxley Act of 2002, or the Sarbanes-Oxley Act,
and rules subsequently implemented by the SEC and The Nasdaq Stock Market LLC have imposed various requirements
on public companies, including establishment and maintenance of effective disclosure and financial controls and corporate
governance practices. Our management and other personnel will need to devote a substantial amount of time to comply
with these requirements. Moreover, these rules and regulations increase our legal and financial compliance costs and make
some activities more time-consuming and costly. For example, we expect that these rules and regulations may make it more
difficult and more expensive for us to obtain director and officer liability insurance.

Pursuant to Section 404 of the Sarbanes-Oxley Act, or Section 404, we will be required to furnish a report by our

management on our internal control over financial reporting, including an attestation report on internal control over
financial reporting issued by our independent registered public accounting firm. However, while we remain an EGC, we
will not be required to include an attestation report on internal control over financial reporting issued by our independent
registered public accounting firm. To achieve compliance with Section 404 within the prescribed period, we will be
engaged in a process to document and evaluate our internal control over financial reporting, which is both costly and
challenging. In this regard, we will need to continue to dedicate internal resources, potentially engage outside consultants
and adopt a detailed work plan to assess and document the adequacy of internal control over financial reporting, continue
steps to improve control processes as appropriate, validate through testing that controls are functioning as documented and
implement a continuous reporting and improvement process for internal control over financial reporting. Despite our
efforts, there is a risk that neither we nor our independent registered public accounting firm will be able to conclude within
the prescribed timeframe that our internal control over financial reporting is effective as required by Section 404. This
could result in an adverse reaction in the financial markets due to a loss of confidence in the reliability of our financial
statements.

Provisions in our corporate charter documents and under Delaware law could make an acquisition of us,

which may be beneficial to our stockholders, more difficult and may prevent attempts by our stockholders to replace or
remove our current management.

Provisions in our corporate charter and our bylaws may discourage, delay or prevent a merger, acquisition or other

change in control of us that stockholders may consider favorable, including transactions in which you might otherwise
receive a premium for your shares. These provisions also could limit the price that investors might be willing to pay in the
future for shares of our common stock, thereby depressing the market price of our common stock. In addition, because our
board of directors is responsible for appointing the members of our management team, these provisions may frustrate or
prevent any attempts by our stockholders to replace or remove our current management by making it more difficult for
stockholders to replace members of our board of directors. Among other things, these provisions:

● establish a classified board of directors such that not all members of the board are elected at one time;
● allow the authorized number of our directors to be changed only by resolution of our board of directors;
● limit the manner in which stockholders can remove directors from the board;
● establish advance notice requirements for stockholder proposals that can be acted on at stockholder meetings

and nominations to our board of directors;

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● require that stockholder actions must be effected at a duly called stockholder meeting and prohibit actions by

our stockholders by written consent;
● limit who may call stockholder meetings;
● authorize our board of directors to issue preferred stock without stockholder approval, which could be used

to institute a stockholder rights plan, or so-called “poison pill,” that would work to dilute the stock ownership
of a potential hostile acquirer, effectively preventing acquisitions that have not been approved by our board
of directors; and

● require the approval of the holders of at least 662/3% of the votes that all our stockholders would be entitled

to cast to amend or repeal certain provisions of our charter or bylaws.

Moreover, because we are incorporated in Delaware, we are governed by the provisions of Section 203 of the

Delaware General Corporation Law, or DGCL, which prohibits a person who owns in excess of 15% of our outstanding
voting stock from merging or combining with us for a period of three years after the date of the transaction in which the 
person acquired in excess of 15% of our outstanding voting stock, unless the merger or combination is approved in a 
prescribed manner.  These provisions could discourage potential acquisition proposals and could delay or prevent a change 
in control transaction. They could also have the effect of discouraging others from making tender offers for our common 
stock, including transactions that may be in your best interests. These provisions may also prevent changes in our 
management or limit the price that investors are willing to pay for our stock.

Our governing documents designate certain courts as the sole and exclusive forum for certain types of actions

and proceedings that may be initiated by our stockholders, which could limit our stockholders’ ability to obtain a
favorable judicial forum for disputes with us or our directors, officers or employees.

Our amended and restated certificate of incorporation provides that, with respect to any state actions or
proceedings under Delaware statutory or common law, the Court of Chancery of the State of Delaware is the exclusive
forum for:

● any derivative action or proceeding brought on our behalf;
● any action asserting a breach of fiduciary duty;
● any action asserting a claim against us or any of our directors, officers, employees or agents arising under the

DGCL, our amended and restated certificate of incorporation or our amended and restated bylaws;

● any action or proceeding to interpret, apply, enforce or determine the validity of our amended and restated

certificate of incorporation or our amended and restated bylaws; and

● any action asserting a claim against us or any of our directors, officers, employees or agents that is governed

by the internal-affairs doctrine.

In addition, our amended and restated bylaws provide that, unless we consent in writing to the selection of an

alternative forum, the federal district courts of the United States are, to the fullest extent permitted by law, the exclusive
forum for the resolution of any complaint asserting a cause of action arising under the Securities Act.

These exclusive-forum provisions may limit a stockholder’s ability to bring a claim in a judicial forum that it finds

favorable for disputes with us or our directors, officers or other employees, which may discourage lawsuits against us and
our directors, officers and other employees. If a court were to find an exclusive-forum provision in our amended and
restated certificate of incorporation or our amended and restated bylaws to be inapplicable or unenforceable in an action,
we may incur additional costs associated with resolving the dispute in other jurisdictions, which could harm our business.

ITEM 1B.      UNRESOLVED STAFF COMMENTS.

None.

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ITEM 2.      PROPERTIES.

Our corporate headquarters are located at 545 Fifth Ave, Suite 1400, New York, NY 10017 where we lease office

space pursuant to a lease agreement that commenced on October 31, 2019 and expires on October 31, 2024. We also
occupy space for offices in Englewood Cliffs, New Jersey pursuant to a lease which commenced on November 1, 2020 for
a three year period. We believe that our existing facilities are suitable and adequate to meet our current needs. We intend to
add new facilities or expand existing facilities as we add employees, and we believe that suitable additional or substitute
space will be available as needed to accommodate any such expansion of our operations.

ITEM 3.      LEGAL PROCEEDINGS.

We are not a party to any material legal proceedings, and we are not aware of any material claims or actions

pending or threatened against us. In the future, we might from time to time become involved in litigation relating to claims
arising from our ordinary course of business, the resolution of which we do not anticipate would have a material adverse
impact on our financial position, results of operations or cash flows.

ITEM 4.      MINE SAFETY DISCLOSURES.

Not applicable.

PART II

ITEM 5.      MARKET FOR REGISTRANT’S COMMON EQUITY, RELATED STOCKHOLDER MATTERS

AND ISSUER PURCHASES OF EQUITY SECURITIES.

Market Information

On  May 16, 2019, our common stock began trading on the Nasdaq Global Market under the symbol “APLT.” 

Prior to that time, there was no public market for our common stock.

Stockholders

As of December 31, 2022, there were approximately 20 stockholders of record of our common stock. The actual
number of holders of our common stock is greater than this number of record holders, and includes stockholders who are
beneficial owners, but whose shares are held in street names by brokers or held by other nominees. This number of holders
of record also does not include stockholders whose shares may be held in trust by other entities.

Dividend Policy

We have never paid or declared any cash dividends on our common stock, and we do not anticipate paying any

cash dividends on our common stock in the foreseeable future. We intend to retain all available funds and any future
earnings to fund the development and expansion of our business. Any future determination to pay dividends will be at the
discretion of our board of directors and will depend upon a number of factors, including our results of operations, financial
condition, future prospects, contractual restrictions, restrictions imposed by applicable law and other factors that our board
of directors deems relevant.

Recent Sales of Unregistered Securities

None.

Issuer Purchases of Equity Securities

We did not purchase any of our registered equity securities during the period covered by this Annual Report.

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ITEM 6.      RESERVED.

ITEM 7.      MANAGEMENT’S DISCUSSION AND ANALYSIS OF FINANCIAL CONDITION AND RESULTS

OF OPERATIONS.

You should read the following discussion and analysis of our financial condition and results of operations together

with our financial statements and the related notes included elsewhere in this Annual Report. Some of the information
contained in this discussion and analysis or set forth elsewhere in this Annual Report, including information with respect to
our plans and strategy for our business and related financing, includes forward-looking statements that involve risks and
uncertainties. As a result of many factors, including those factors set forth in the “Risk Factors” section of this Annual
Report, our actual results could differ materially from the results described in or implied by these forward-looking
statements.

Overview

We are a clinical-stage biopharmaceutical company developing a pipeline of novel product candidates against

validated molecular targets in indications of high unmet medical need. We focus on molecules and pathways whose role in
the disease process is well known based on prior research, but have previously failed to yield successful products due to
poor efficacy and tolerability. Our unique approach to drug development leverages recent technological advances to design
improved drugs, employs early use of biomarkers to confirm biological activity and focuses on abbreviated regulatory
pathways. Our first molecular target is aldose reductase, or AR, an enzyme that converts glucose to sorbitol under oxidative
stress conditions, and is implicated in multiple diseases. Prior attempts to inhibit this enzyme were hindered by
nonselective, nonspecific inhibition, which resulted in limited efficacy and significant off-target safety effects. The
detrimental consequences of AR activation have been well established by decades of prior research. Our AR program
currently includes three small molecules, which are all potent and selective inhibitors of AR, but are engineered to have
unique tissue permeability profiles to target different disease states, including diabetic complications, heart disease and rare
metabolic diseases. The result of this unique multifaceted approach to drug development is a portfolio of highly specific
and selective product candidates that we believe are significantly de-risked and can move quickly through the development
process.

AT-007 is a novel central nervous system, or CNS, penetrant ARI that we are developing for the treatment of rare 
metabolic diseases, including Galactosemia and SORD Deficiency.  Galactosemia is a devastating rare pediatric metabolic 
disease that affects how the body processes a simple sugar called galactose, and for which there is no known cure or 
approved treatment available. The U.S. Food and Drug Administration, or FDA, has granted both orphan drug designation 
and rare pediatric disease designation to AT-007 for the treatment of Galactosemia and in June 2021, the FDA granted Fast 
Track Designation to AT-007 for the treatment of Galactosemia. We have completed an adult study in healthy volunteers 
and Galactosemia patients, demonstrating that AT-007 is safe and well tolerated, and significantly reduces plasma galactitol 
levels vs. placebo. Galactitol is a toxic metabolite of galactose, which is formed in Galactosemia patients by aberrant 
activity of aldose reductase when galactose is present at high levels. A pediatric study is underway in children with 
Galactosemia, assessing the impact of AT-007 vs. placebo on safety, biomarker reduction of galactitol, and long-term 
functional outcomes. On April 13, 2021, we presented data featuring a cross-sectional analysis of nineteen pediatric 
patients with Classic Galactosemia, providing meaningful insight on the progressive worsening of the central nervous 
system phenotype with age. On October 18, 2021, we reported biomarker data from the pediatric ACTION-Galactosemia 
Kids study. The results demonstrate a substantial reduction in plasma galactitol of approximately 40%, which was 
statistically significant (p<0.001) vs. placebo. We previously reported a baseline analysis of the 47 children enrolled in the 
study which demonstrated a clear correlation between baseline galactitol levels and baseline clinical functional outcomes. 
The long-term functional outcomes portion of the pediatric study is ongoing, and the outcomes are assessed every 6 months 
by a fire-walled data monitoring committee (DMC).  When the study reaches statistical significance in the active treated 
arm vs. the placebo arm, the DMC will alert the Company and the trial will be unblinded.  In April 2022, the Company met 
with the FDA to discuss the design of the ongoing pediatric study prior to the first 6-month outcomes assessment by the 
DMC.  The FDA confirmed that the pediatric study as it is currently designed would support an NDA submission if 
statistical significance is reached, and there is alignment between the FDA and the Company on the potential path forward 
to approval.  The 12-month clinical outcomes were assessed by the 

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fire-walled DMC, and as expected the data did not yet reach statistical significance, but demonstrated a trend in clinical 
outcomes favoring AT-007 vs. placebo.  A safety analysis showed that AT-007 continued to be safe and well tolerated.   
The Company is exploring a potential submission for conditional approval based on existing data with the European 
Medicines Agency (EMA).

AT-007 is also being studied in a rare disease caused by deficiency in the enzyme Sorbitol Dehydrogenase. Aldose 

Reductase is the first enzyme in the polyol pathway, converting glucose to sorbitol. AR is then followed by Sorbitol 
Dehydrogenase, which converts sorbitol to fructose. Patients with SORD Deficiency accumulate very high levels of 
sorbitol in their cells and tissues as a result of the enzyme deficiency, which results in tissue toxicities such as peripheral 
neuropathy and motor neuron disease. Recent research in drosophila and cell models of SORD Deficiency demonstrated 
that treatment with an ARI that blocks sorbitol production may provide benefit in this disease. Preclinical studies on AT-
007 have demonstrated significant reduction in sorbitol levels in fibroblasts from SORD deficient patients. Treatment with 
AT-007 in the drosophila model of SORD  prevented the disease phenotype and protected from neuronal degeneration. On 
October 25, 2021, we reported data from a pilot open-label study in 8 SORD Deficiency patients. AT-007 reduced blood 
sorbitol levels by approximately 66% from baseline through 30 days of treatment. AT-007 was safe and well tolerated in all 
treated patients. In December 2021, we initiated a Phase 2/3 registrational study in patients with SORD Deficiency, which 
is ongoing at multiple clinical sites in the US and Europe. On February 16, 2023, we announced that in a pre-specified 
interim analysis of the ongoing Phase 3 INSPIRE trial, AT-007 reduced sorbitol levels by a mean of approximately 52% (or 
approximately 16,000ng/ml) over 90 days of treatment (p<0.001 vs. placebo) in patients with SORD Deficiency. At 
baseline, the mean blood sorbitol level of SORD patients included in this interim analysis was approximately 29,000ng/ml, 
with a range of approximately 22,000ng/ml-38,000ng/ml. In the INSPIRE trial, a baseline cross-sectional analysis of the 
relationship between sorbitol level, age (or duration of disease) and clinical outcome measures demonstrated a statistically 
significant correlation between sorbitol level and key clinical outcome measures, including 10-meter-walk/run speed, 4-
stair climb speed, and sit-to-stand test (p<0.05). The Company is working with the FDA to determine the appropriate 
regulatory path forward, as well as data required for an NDA submission,  to advance AT-007 towards registration for this 
indication.  The INSPIRE study will continue in blinded format to the 12-month interim clinical outcomes assessment. If 
the primary clinical outcome measure (10-meter-walk/run) reaches statistical significance at 12 months, the study will be 
completed and unblinded. If not, the study will continue in blinded format to 24 months, where clinical outcomes will be 
assessed again in a final statistical analysis. AT-007 continues to be safe and well tolerated to date.

We also plan to initiate a clinical development program on AT-007 in another pediatric rare disease, called PMM2-
CDG. PMM2-CDG is a glycosylation disorder caused by deficiencies in the enzyme phosphomannomutase 2, which leads 
to CNS symptoms similar to Galactosemia, including low IQ, tremor, and speech and motor problems.  Aldose Reductase 
is over-activated in this disease as a compensatory consequence of PMM2 deficiency, and a CNS penetrant ARI may be a 
compelling clinical option. Initial data in fibroblast cell lines derived from PMM2-CDG patients demonstrates that AT-007 
treatment increases phosphomannomutase 2 activity. The FDA has granted pediatric rare disease designation and orphan 
designation for AT-007 in PMM2-CDG. 

AT-001 is a novel ARI with broad systemic exposure and peripheral nerve permeability that we are developing for
the treatment of diabetic cardiomyopathy, or DbCM, a fatal fibrosis of the heart, for which no treatments are available. We
completed a Phase 1/2 clinical trial evaluating AT-001 in approximately 120 patients with type 2 diabetes, in which no
drug-related adverse effects or tolerability issues were observed. In September 2019, we announced the initiation of a
Phase 3 registrational trial of AT-001 in DbCM. The study, called ARISE-HF, is designed to evaluate AT-001’s ability to
improve or prevent the decline of functional capacity in patients with DbCM at high risk of progression to overt heart
failure. Although we did experience enrollment delays in 2020 associated with the Covid-19 pandemic, modifications were
made to the trial to include additional sites and geographies to address Covid-19-related issues. The trial is now fully
enrolled with 675 patients.

AT-003 is a novel ARI designed to cross through the back of the eye when dosed orally, and has demonstrated

strong retinal penetrance, for the treatment of diabetic retinopathy, or DR. DR is an ophthalmic disease that occurs in
diabetic patients and for which treatments are currently limited to high-cost biologics requiring intravitreal administration.
DR has been linked to AR activity, including elevations in sorbitol and subsequent changes in retinal blood vessels, which
distorts vision and leads to permanent blindness.

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AT-104 is a preclinical dual selective PI3K inhibitor.  Due to recent regulatory changes impacting development of 
the PI3K inhibitor class of compounds, the Company has discontinued its early stage preclinical PI3K program and further 
development of AT-104. The compound and all rights associated with the technology were returned to Columbia
University.

Since inception in 2016, our operations have focused on developing our product candidates, organizing and

staffing our company, business planning, raising capital, establishing our intellectual property portfolio and conducting
clinical trials. We do not have any product candidates approved for sale and have not generated any revenue.

We have incurred significant operating losses since inception in 2016. Our ability to generate product revenue

sufficient to achieve profitability will depend on the successful development and commercialization of one or more of our
product candidates. Our net loss was $82.5 million for the year ended December 31, 2022. As of December 31, 2022, we
had an accumulated deficit of $348.8 million. We expect to continue to incur significant expenses and increasing operating
losses for the foreseeable future in connection with our ongoing activities. Furthermore, we expect to incur additional costs
associated with operating as a public company, including significant legal, accounting, investor relations and other
expenses. As of December 31, 2022, we had cash and cash equivalents and short-term investments of $30.6 million.

February 2021 Secondary Public Offering

In February 2021, we issued and sold 3,000,000 shares of common stock at a public offering price of $23.00 per 

share, with an additional 450,000 shares sold pursuant to the underwriters’ full exercise of their option to purchase 
additional shares in the February Offering.  We received aggregate proceeds, net of underwriting discounts and 
commissions and offering costs of $74.4 million.

June 2022 Offering

On June 27, 2022, the Company completed the June Offering, an underwritten public offering of 20,000,000
shares of common stock, par value $0.0001 per share, 10,000,000 Pre-Funded Warrants, and accompanying Common
Warrants to purchase up to 30,000,000 shares of common stock. The shares and accompanying Common Warrants were
offered at a price to the public of $1.00 per share and warrant, and the Pre-Funded Warrants and accompanying Common
Warrants were offered at a price to the public of $0.9999, resulting in aggregate net proceeds of approximately $27.8
million, after deducting underwriting discounts and commissions and offering expenses. The Pre-Funded Warrants and the
Common Warrants are immediately exercisable and will expire five years from the date of issuance. Holders may not
exercise any Pre-Funded Warrants or Common Warrants that would cause the aggregate number of shares of common
stock beneficially owned by the holder to exceed 9.99% of the Company’s outstanding common stock immediately after
exercise. Holders of the Pre-Funded Warrants and/or Common Warrants (together with affiliates) who immediately prior to
June 27, 2022 beneficially owned more than 9.99% of the Company’s outstanding common stock may not exercise any
portion of their Pre-Funded Warrants or Common Warrants if the holder (together with affiliates) would beneficially own
more than 19.99% of the Company’s outstanding common stock after exercise. The Pre-Funded Warrants and Common
Warrants are subject to adjustment in the event of certain stock dividends and distributions, stock splits, stock
combinations, reclassifications or similar events affecting the common stock and also upon any distributions for no
consideration of assets to the Company’s stockholders. In the event of certain corporate transactions, the holders of the Pre-
Funded Warrants and/or Common Warrants will be entitled to receive, upon exercise, the kind and amount of securities,
cash or other property that the holders would have received had they exercised the Pre-Funded Warrants and/or Common
Warrants immediately prior to such transaction. The Pre-Funded Warrants and Common Warrants do not entitle the holders
thereof to any voting rights or any of the other rights or privileges to which the Company’s stockholders are entitled. The
Company intends to use the net proceeds from the June Offering for general corporate purposes, which may include
research and development costs, including the conduct of clinical trials and process development and manufacturing of the
Company’s product candidates, expansion of the Company’s research and development capabilities, working capital and
capital expenditures.

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Components of Our Results of Operations

Revenue

Since inception, we have not generated any revenue and do not expect to generate any revenue from the sale of
products in the near future. If our development efforts for our product candidates are successful and result in regulatory
approval, or if we enter into collaboration or license agreements with third parties, we may generate revenue in the future
from a combination of product sales or payments from collaboration or license agreements.

Operating Expenses

Research and Development Expenses

Research and development expenses consist primarily of costs incurred for our research activities, including our

discovery efforts and the development of our product candidates, and include:

● employee-related expenses, including salaries, related benefits and stock-based compensation expense for

employees engaged in research and development functions;

● fees paid to consultants for services directly related to our product development and regulatory efforts;

● expenses incurred under agreements with contract research organizations, or CROs, as well as contract

manufacturing organizations, or CMOs, and consultants that conduct and provide supplies for our preclinical
studies and clinical trials;

● costs associated with preclinical activities and development activities;

● costs associated with our technology and our intellectual property portfolio; and

● costs related to compliance with regulatory requirements.

We expense research and development costs as incurred. Costs for external development activities are recognized

based on an evaluation of the progress to completion of specific tasks using information provided to us by our vendors.
Payments for these activities are based on the terms of the individual agreements, which may differ from the pattern of
costs incurred, and are reflected in our financial statements as prepaid or accrued research and development expenses.

Research and development costs also include costs incurred in connection with certain licensing arrangements.
Before a compound receives regulatory approval, we record upfront and milestone payments made by us to third parties
under licensing arrangements as expense. Upfront payments are recorded when incurred, and milestone payments are
recorded when the specific milestone has been achieved. Once a compound receives regulatory approval, we will record
any milestone payments in Identifiable intangible assets, less accumulated amortization and, unless the asset is determined
to have an indefinite life, we will amortize the payments on a straight-line basis over the remaining agreement term or the
expected product life cycle, whichever is shorter.

Research and development activities are central to our business model. We expect that our research and

development expenses will continue to increase for the foreseeable future as we continue clinical development for our
product candidates and continue to discover and develop additional product candidates. If any of our product candidates
enter into later stages of clinical development, they will generally have higher development costs than those in earlier
stages of clinical development, primarily due to the increased size and duration of later-stage clinical trials. Historically, we
have incurred research and development expenses that primarily relate to the development of AT-007, AT-001 and our ARI
program. As we advance our product candidates, we expect to allocate our direct external research and development costs
across each of the indications or product candidates.

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The following table summarizes our research and development expenses for the years ended December 31, 2022

and 2021:

(in thousands)
Product pipeline research and development expenses

AT-001
AT-007

Personnel-related expenses
Stock-based compensation
Other expenses
Total research and development expenses

General and Administrative Expenses

Year Ended
December 31, 

2022

2021

$

$

 20,809
 23,902
 6,648
 3,618
 657
 55,634

$

$

 22,861
 30,669
 5,529
 2,759
 752
 62,570

General and administrative expenses consist primarily of salaries and other related costs, including stock-based

compensation, for personnel in our executive, finance, and commercial functions. General and administrative expenses also
include professional fees for legal, accounting, auditing, tax and consulting services; travel expenses; and facility-related
expenses, which include allocated expenses for rent and maintenance of facilities and other operating costs.

Commercial expenses consist of payroll expense for commercial personnel, as well as marketing, market research,

market access, and other focused investments to support launch of drug candidates, generate evidence of commercial
potential and value proposition, and maximize potential business development deal leverage. Commercial expenses are
included in general and administrative expenses.

We expect that our general and administrative expenses will increase in the future as we increase our general and

administrative headcount to support our continued research and development and potential commercialization of our
product candidates. We also expect to incur increased expenses associated with being a public company, including costs of
accounting, audit, legal, regulatory and tax compliance services; director and officer insurance costs; and investor and
public relations costs.

Other Income (Expense), Net

Other income (expense), net consists of interest income (expense), net, and other income (expense), net. Interest

income (expense), net consists primarily of our interest income on our cash and cash equivalents and marketable securities.
Other income (expense), net consists primarily of realized gains and losses on sales of marketable securities.

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Results of Operations

The following table summarizes our results of operations:

(in thousands)
Operating expenses:

Research and development
General and administrative
Total operating expenses

Loss from operations
Other income (expense), net:

Interest income (expense), net
Change in fair value of warrant liabilities
Other income (expense)

Other income (expense), net

Net loss

Research and Development Expenses

Years Ended

December 31, 

2022

2021

$  55,634
 27,316
 82,950
   (82,950)

$  62,570
 43,048
 105,618
   (105,618)

 685
 (66)
 (177)
 442

 555
 —
 (521)
 34
$ (82,508) $  (105,584)

The following table summarizes our research and development expenses:

(in thousands)
Clinical and pre-clinical
Drug manufacturing and formulation
Personnel expenses
Stock-based compensation
Regulatory and other
Total research and development expenses

Year Ended
December 31, 

2022
$ 42,928
 957
 6,648
 3,619
 1,482
$ 55,634

2021
$ 40,323
 11,910
 5,529
 2,759
 2,049
$ 62,570

$

     Increase / (Decrease)
 2,605
 (10,953)
 1,119
 860
 (567)
 (6,936)

$

Research and development expenses for the year ended December 31, 2022 were $55.6 million, compared to

$62.6 million for the year ended December 31, 2021. The decrease of approximately $6.9 million was primarily related to:

● an increase in clinical and pre-clinical expense of $2.6 million, primarily related to the progression of
the SORD Phase 2/3 registrational study, progression of the AT-007 ACTION-Galactosemia long-term
extension adult study, and progression of the AT-007 ACTION-Galactosemia Kids pediatric
registrational study;

● a decrease in drug manufacturing and formulation expenses of $11.0 million primarily related to the
completion and release of AT-001 and AT-007 drug product batches in the year ended December 31,
2021;

● an increase in personnel expenses of $1.1 million due to the increase in headcount in support of our

clinical program pipeline;

● an increase in stock-based compensation of $0.9 million due to new stock option and restricted stock

unit grants, offset by forfeitures of stock option and restricted stock unit grants;

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● a decrease of regulatory and other expenses of $0.6 million primarily related to the UM license fees

recognized during the year ended December 31, 2021.

General and Administrative Expenses

The following table summarizes our general and administrative expenses:

(in thousands)
Legal and professional fees
Commercial expenses
Personnel expenses
Stock-based compensation
Insurance expenses
Other expenses
Total general and administrative expenses

Year Ended
December 31, 

2022
$  6,854
 2,193
 5,537
 5,543
 3,682
 3,507
$ 27,316

2021
$  6,340
 11,341
 6,617
 8,418
 4,399
 5,933
$ 43,048

$

     Increase / (Decrease)
 514
 (9,148)
 (1,080)
 (2,875)
 (717)
 (2,426)
 (15,732)

$

General and administrative expenses were $27.3 million for the year ended December 31, 2022, compared to

$43.0 million for the year ended December 31, 2021. The decrease of approximately $15.7 million was primarily related
to:

● an increase in professional and legal fees of $0.5 million due to higher external legal fees;

● a decrease of $9.1 million related to decreased spend for commercial operations;

● a decrease in personnel expenses of $1.1 million and a decrease in stock-based compensation of $2.9  

million due to a decrease in headcount;

● a decrease of insurance expenses of $0.7 million related to decreased directors and officers liability

insurance costs; and

● a decrease in other expenses of $2.4 million, primarily relating to decreased costs of other office

expenses.

Other Income (Expense), Net

Interest income was $0.7 million for the year ended December 31, 2022 as compared to $0.6 million for the year 

ended December 31, 2021.  Interest income is derived from our marketable securities and the increase of $0.1 million in 
interest income year over year is due to rising interest rates during 2022. 

Change in fair value of warrant liabilities - The change in the fair value of our warrant liabilities for the year

ended December 31, 2022 resulted in a $0.1 million expense recognized in the period. There were no warrant liabilities for
the year ended December 31, 2021.

Other expense, net was expense of approximately $0.2 million for the year ended December 31, 2022, compared

to expense of $0.5 million for the year ended December 31, 2021. The decrease was primarily related to lower realized
losses incurred by our available-for-sale securities portfolio during the year ended December 31, 2022.

Liquidity and Capital Resources

Since our inception through December 31, 2022, we have not generated any revenue and have incurred significant

operating losses and negative cash flows from our operations. The accompanying financial statements have

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been prepared assuming the continuation of the Company as a going concern. The exclusive licensing agreement with 
Advanz  Pharma for commercialization rights to  AT-007 in Europe is expected to provide a source of  capital to the 
Company based on clinical and regulatory milestones. If  actualization of these milestones aligns with the projected 
timelines, and product approvals are received in the timeframes expected, this source of capital may be sufficient to cover 
operating expenses through expected product approvals and potential revenues. However,  there are no guarantees that this 
will materialize, and delays or unexpected  data  could disrupt this potential source of liquidity. Broadly, the Company has 
not yet established an ongoing source of revenues sufficient to cover its operating costs and is dependent on debt and 
equity financing to fund its operations. As of December 31, 2022, our cash, cash equivalents and marketable securities was
$30.6 million. We also received a $10.7 million upfront payment from Advanz Pharma in January 2023 in conjunction with 
signing the exclusive licensing agreement for European commercialization rights.  We believe that our cash and cash 
equivalents as of December 31, 2022, along with the upfront payment received in January 2023 and the projected clinical 
and regulatory milestone payments expected in fiscal year 2023 from Advanz Pharma will be sufficient to fund our 
operations through year end 2023, and potentially beyond if clinical trial completion and marketing authorization in Europe 
as well as commercial sales milestones materialize in the expected timelines. The report of our independent registered 
public accounting firm on our financial statements for the year ended December 31, 2022 includes an explanatory 
paragraph regarding the existence of substantial doubt about our ability to continue as a going concern. Given our planned 
expenditures for the next several years, we have concluded and our independent registered public accounting firm has 
agreed with our conclusion that there is still a substantial doubt regarding our ability to continue as a going concern for a
period of 12 months beyond the filing of this Form 10-K.

Cash Flows

The following table summarizes our cash flows for each of the periods presented:

(in thousands)
Net cash used in operating activities
Net cash provided by/(used in) investing activities
Net cash provided by financing activities

Net increase (decrease) in cash and cash equivalents

Operating Activities

Year Ended
December 31, 

2022

2021

$ (78,093) $  (90,728)
 12,433
 74,717
$ (37,231) $  (3,578)

 13,170
 27,692

During the year ended December 31, 2022, operating activities used cash of $78.1 million, due to our net losses of

$82.6 million, a decrease in operating lease liability of $0.4 million, a decrease in financed insurance premium of $3.1
million, a decrease of $1.6 million in accrued expense, and a decrease in accounts payable of $4.9 million. This is partially
offset by increases of $0.4 million in prepaid expense, $0.4 million of issuance of options in-lieu of bonus, $9.2 million in
non-cash stock-based compensation expense, and $3.6 million of amortization of insurance premium, an increase of $0.1
million in change in fair value of warrant liability, and $0.4 million in amortization of operating lease right-of-use assets.

During the year ended December 31, 2021, operating activities used cash of $90.7 million, due to our net losses of

$105.6 million, a decrease in operating lease liability of $0.4 million, a decrease in financed insurance premium of $4.4
million, a decrease of $3.3 million in accrued expense, and a decrease in prepaid expenses of $1.7 million. This is partially
offset by increases of $8.8 million in accounts payable, $11.2 million in non-cash stock-based compensation expense, and
$4.3 million of amortization of insurance premium, and $0.4 million in amortization of operating lease right-of-use assets.

Investing Activities

Net cash provided by investing activities for the year ended December 31, 2022 was $13.2 million relating to our

purchases of available-for-sale marketable securities for $64.2 million and proceeds from the maturities of available-for-
sale marketable securities for $77.4 million.

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Net cash provided by investing activities for the year ended December 31, 2021 was $12.4 million relating to our

purchases of available-for-sale marketable securities for $121.6 million and proceeds from the sale and maturities of
available-for-sale marketable securities for $134.0 million.

Financing Activities

During the year ended December 31, 2022, net cash provided by financing activities was $27.7 million, primarily

from the cash proceeds from the June 2022 offering of $27.8 million, $49,000 from the exercise of stock options for
common stock under the 2019 Plan, and $3.1 million from the proceeds from financed insurance premium. This was
partially offset by the repayment of short-term borrowings of $3.3 million.

In June 2020, we entered into the Goldman Equity Distribution Agreement to sell shares of our common stock,

from time to time, having an aggregate offering price of up to $100 million. The Goldman Equity Distribution Agreement
was terminated as of January 24, 2022.

On January 26, 2022, the Company entered into the Cowen Equity Distribution Agreement to sell shares of the
Company’s common stock, from time to time, having an aggregate offering price of up to $100.0 million. Pursuant to the
Cowen Equity Distribution Agreement shares of our common stock may be offered and sold through the sales agent in
sales deemed “at-the-market” offerings under the Securities Act of 1933, as amended, or the Securities Act. Under the
Cowen Equity Distribution Agreement, the sales agent will be entitled to compensation of up to 3% of the gross offering
proceeds of all shares of our common stock sold through it pursuant to the Cowen Equity Distribution Agreement. In
connection with the sale of shares of our common stock on our behalf, the sales agent may be deemed to be “underwriters”
within the meaning of the Securities Act, and the compensation paid to the sales agent may be deemed to be underwriting
commissions or discounts. As of December 31, 2022, the Company has not sold any shares of common stock pursuant to
the Cowen Equity Distribution Agreement.

On June 27, 2022, the Company completed the June Offering, an underwritten public offering of 20,000,000
shares of common stock, par value $0.0001 per share, 10,000,000 Pre-Funded Warrants, and accompanying Common
Warrants to purchase up to 30,000,000 shares of common stock. The shares and accompanying Common Warrants were
offered at a price to the public of $1.00 per share and warrant, and the Pre-Funded Warrants and accompanying Common
Warrants were offered at a price to the public of $0.9999, resulting in aggregate net proceeds of approximately $27.8
million, after deducting underwriting discounts and commissions and offering expenses. The Pre-Funded Warrants and the
Common Warrants are immediately exercisable and will expire five years from the date of issuance. Holders may not
exercise any Pre-Funded Warrants or Common Warrants that would cause the aggregate number of shares of common
stock beneficially owned by the holder to exceed 9.99% of the Company’s outstanding common stock immediately after
exercise. Holders of the Pre-Funded Warrants and/or Common Warrants (together with affiliates) who immediately prior to
June 27, 2022 beneficially owned more than 9.99% of the Company’s outstanding common stock may not exercise any
portion of their Pre-Funded Warrants or Common Warrants if the holder (together with affiliates) would beneficially own
more than 19.99% of the Company’s outstanding common stock after exercise. The Pre-Funded Warrants and Common
Warrants are subject to adjustment in the event of certain stock dividends and distributions, stock splits, stock
combinations, reclassifications or similar events affecting the common stock and also upon any distributions for no
consideration of assets to the Company’s stockholders. In the event of certain corporate transactions, the holders of the Pre-
Funded Warrants and/or Common Warrants will be entitled to receive, upon exercise, the kind and amount of securities,
cash or other property that the holders would have received had they exercised the Pre-Funded Warrants and/or Common
Warrants immediately prior to such transaction. The Pre-Funded Warrants and Common Warrants do not entitle the holders
thereof to any voting rights or any of the other rights or privileges to which the Company’s stockholders are entitled. The
Company intends to use the net proceeds from the June Offering for general corporate purposes, which may include
research and development costs, including the conduct of clinical trials and process development and manufacturing of the
Company’s product candidates, expansion of the Company’s research and development capabilities, working capital and
capital expenditures.

During the year ended December 31, 2021, net cash provided by financing activities was $74.7 million, primarily

from the cash proceeds from the secondary offering of $74.4 million, $0.5 million from the exercise of stock options for
common stock under the 2019 Plan, and $69,000 from the exercise of warrants for common stock, and $4.4

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million from the proceeds from financed insurance premium. This was partially offset by the repayment of short-term
borrowings of $4.7 million.

Funding Requirements

We expect our expenses to increase substantially in connection with our ongoing activities, particularly as we

advance the preclinical activities and clinical trials of our product candidates. We believe that our expenses may increase
significantly if and as we:

● continue the ongoing and planned development of our product candidates;
● initiate, conduct and complete any ongoing, anticipated or future preclinical studies and clinical trials for our

current and future product candidates;

● seek marketing approvals for any product candidates that successfully complete clinical trials;
● establish a sales, marketing, manufacturing and distribution infrastructure to commercialize any current or

future product candidate for which we may obtain marketing approval;

● seek to discover and develop additional product candidates;
● continue to build a portfolio of product candidates through the acquisition or in-license of drugs, product

candidates or technologies;

● maintain, protect and expand our intellectual property portfolio;
● hire additional clinical, regulatory and scientific personnel; and
● add operational, financial and management information systems and personnel, including personnel to

support our product development and planned future commercialization efforts.

Furthermore, we have and expect to incur additional costs associated with operating as a public company,

including significant legal, accounting, investor relations and other expenses.

Due to the numerous risks and uncertainties associated with the development of our product candidates and
programs, and because the extent to which we may enter into collaborations with third parties for development of our
product candidates is unknown, we are unable to estimate the timing and amounts of increased capital outlays and
operating expenses associated with completing the research and development of our product candidates. Our future funding
requirements, both near and long-term, will depend on many factors, including:

● the initiation, scope, progress, timing, costs and results of our ongoing and planned clinical trials for our

product candidates;

● the outcome, timing and cost of meeting regulatory requirements established by the FDA and other

comparable foreign regulatory authorities;

● the cost of filing, prosecuting, defending and enforcing our patent claims and other intellectual property

rights;

● the cost of defending potential intellectual property disputes, including patent infringement actions;
● the achievement of milestones or occurrence of other developments that trigger payments under the  

Columbia Agreements or other agreements we may enter into;

● the extent to which we are obligated to reimburse, or entitled to reimbursement of, clinical trial costs under

future collaboration agreements, if any;

● the effect of competing technological and market developments;
● the cost and timing of completion of clinical or commercial-scale manufacturing activities;
● the costs of operating as a public company;
● the extent to which we in-license or acquire other products and technologies;
● our ability to establish and maintain collaborations on favorable terms, if at all;
● the cost of establishing sales, marketing and distribution capabilities for our product candidates in regions

where we choose to commercialize our product candidates, if approved; and

● the initiation, progress, timing and results of the commercialization our product candidates, if approved, for

commercial sale.

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A change in the outcome of any of these variables with respect to the development of a product candidate could

mean a significant change in the costs and timing associated with the development of that product candidate.

Until such time, if ever, that we can generate product revenue sufficient to achieve profitability, we expect to

finance our cash needs through offerings of securities, PIPE, debt financings, collaborations or other strategic transactions.
The terms of financing may adversely affect the holdings or the rights of our stockholders. Funding may not be available to
us on acceptable terms, or at all. If we are unable to obtain funding, we may be required to delay, limit, reduce or terminate
some or all of our research and product development, product portfolio expansion or future commercialization efforts. If
we raise additional capital through debt financing, we may be subject to covenants limiting or restricting our ability to take
specific actions, such as incurring additional debt, making capital expenditures or declaring dividends.

Contractual Obligations and Commitments

The following table summarizes our contractual obligations as of December 31, 2022:

(in thousands)

     Total      1 Year

     1 to 3 Years      4 to 5 Years     

Payments Due By Period

Less Than

More Than
5 Years

Operating lease commitments(1)

$

940

$  515

Total

$

940

$  515

$

$

 425

 425

$

$

 — $

 — $

 —

 —

(1) Represents future minimum lease payments under our operating leases for office space.

Except as disclosed in the table above, we have no long-term debt or capital leases and no material non-cancelable

purchase commitments with service providers, as we have generally contracted on a cancelable, purchase-order basis. We
enter into contracts in the normal course of business with CROs, CMOs and other third parties for clinical trials, preclinical
research studies and testing and manufacturing services. These contracts are cancelable by us upon prior notice. Payments
due upon cancellation consist only of payments for services provided or expenses incurred, including noncancelable
obligations of our service providers, up to the date of cancellation. These payments are not included in the preceding table
as the amount and timing of such payments are not known.

We may incur potential contingent payments upon our achievement of clinical, regulatory and commercial
milestones, as applicable, or royalty payments that we may be required to make under the 2016 and 2019 Columbia
Agreements, the 2020 Miami License Agreement, the 2020 Miami Option Agreement, and the 2020 Miami Research
Agreement, pursuant to which we have in-licensed certain intellectual property. Due to the uncertainty of the achievement
and timing of the events requiring payment under these agreements, the amounts to be paid by us are not fixed or
determinable at this time and are excluded from the table above. See the section titled “Business—Exclusive License
Agreement with Columbia University” and “Business—License Agreement with University of Miami.”

Critical Accounting Policies and Significant Judgments and Estimates

Our management’s discussion and analysis of financial condition and results of operations is based on our

financial statements, which have been prepared in accordance with U.S. generally accepted accounting principles, or
U.S. GAAP. The preparation of our financial statements and related disclosures requires us to make estimates and
assumptions that affect the reported amounts of assets and liabilities, costs and expenses and the disclosure of contingent
assets and liabilities in our financial statements. We base our estimates on historical experience, known trends and events
and various other factors that we believe are reasonable under the circumstances, the results of which form the basis for
making judgments about the carrying values of assets and liabilities that are not readily apparent from other sources. We
evaluate our estimates and assumptions on an ongoing basis. Our actual results may differ from these estimates under
different assumptions or conditions.

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While our significant accounting policies are described in greater detail in Note 1 to our financial statements

appearing elsewhere in this Annual Report, we believe that the following accounting policies are those most critical to the
judgments and estimates used in the preparation of our financial statements.

Accrued Research and Development Expenses

We expense all costs incurred in performing research and development activities. Research and development

expenses include materials and supplies, preclinical expenses, manufacturing expenses, contract services and other outside
expenses. As part of the process of preparing our financial statements, we are required to estimate our accrued research and
development expenses. We make estimates of our accrued expenses as of each balance sheet date in the financial
statements based on facts and circumstances known to us at that time. There may be instances in which payments made to
our vendors will exceed the level of services provided and result in a prepayment of the expense. In accruing service fees,
we estimate the time period over which services will be performed and the level of effort to be expended in each period. If
the actual timing of the performance of services or the level of effort varies from the estimate, we adjust the accrual or the
amount of prepaid expenses accordingly. Although we do not expect our estimates to be materially different from amounts
actually incurred, our understanding of the status and timing of services performed relative to the actual status and timing
of services performed may vary and may result in reporting amounts that are too high or too low in any particular period.
To date, there have not been any material adjustments to our prior estimates of accrued research and development
expenses. Nonrefundable advance payments for goods or services to be received in the future for use in research and
development activities are deferred and capitalized. The capitalized amounts are expensed as the related goods are
delivered or the services are performed.

Research and development costs also include costs incurred in connection with certain licensing arrangements.
Before a compound receives regulatory approval, we record upfront and milestone payments made by us to third parties
under licensing arrangements as expense. Upfront payments are recorded when incurred, and milestone payments are
recorded when the specific milestone has been achieved. Once a compound receives regulatory approval, we will record
any milestone payments in Identifiable intangible assets, less accumulated amortization and, unless the asset is determined
to have an indefinite life, we will amortize the payments on a straight-line basis over the remaining agreement term or the
expected product life cycle, whichever is shorter.

Stock-Based Compensation

We account for our stock-based compensation as expense in the statements of operations based on the awards’

grant date fair values. We account for forfeitures as they occur by reversing any expense recognized for unvested awards.

We estimate the fair value of options granted using the Black-Scholes option pricing model. The Black-Scholes

option pricing model requires inputs based on certain subjective assumptions, including (a) the expected stock price
volatility, (b) the calculation of expected term of the award, (c) the risk-free interest rate and (d) expected dividends. Due to
a historical lack of a public market for our common stock and a lack of company-specific historical and implied volatility
data, we have based our estimate of expected volatility on the historical volatility of a group of similar companies that are
publicly traded. The historical volatility is calculated based on a period of time commensurate with the expected term
assumption. The computation of expected volatility is based on the historical volatility of a representative group of
companies with similar characteristics to us, including stage of product development and life science industry focus. We
use the simplified method as allowed by the SEC Staff Accounting Bulletin No. 107, Share-Based Payment, to calculate
the expected term for options granted as we do not have sufficient historical exercise data to provide a reasonable basis
upon which to estimate the expected term. The risk-free interest rate is based on a treasury instrument whose term is
consistent with the expected term of the stock options. The expected dividend yield is assumed to be zero as we have never
paid dividends and have no current plans to pay any dividends on our common stock. The fair value of stock-based
payments is recognized as expense over the requisite service period which is generally the vesting period.

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Warrant Liabilities

We  account  for  our  Warrant  liabilities  by  measuring  the  fair  value  at  inception  and  are  then  subsequently
measured  on  a  recurring  basis,  with  changes  in  fair  value  recognized  in  other  income  (expense)  within  the  Company’s
statement of operations.

We utilized a Black-Scholes option pricing model to estimate the fair value of the Common and Pre-Funded

Warrants, which utilizes certain unobservable inputs and is therefore considered a Level 3 fair value measurement. Certain
inputs used in this Black-Scholes pricing model may fluctuate in future periods based upon factors that are outside of the
Company’s control, including a potential change in control outside of the Company’s control. A significant change in one
or more of these inputs used in the calculation of the fair value may cause a significant change to the fair value of the
Company’s warrant liabilities, which could also result in material non-cash gains or losses being reported in the Company’s
consolidated statement of operations.

We utilized a probability-weighted approach that considered the probability of a change in control at the Company

in the Black-Scholes option pricing model, whereby a 10% probability of change in control was used for each of the five
years in the term of the agreements.

The inputs we utilized  to value the warrant liability for Common and Pre-Funded Warrants are highly subjective. 
The assumptions used in calculating the fair value of the warrant liability for Common and Pre-Funded Warrants represent 
our best estimates, but these estimates involve inherent uncertainties and the application of management judgment. As a 
result, if factors change and we use different assumptions, the fair value of the warrant liability for Common Warrants may 
be materially different in the future.

Off-Balance Sheet Arrangements

We have not entered into any off-balance sheet arrangements and do not have any holdings in variable interest

entities.

Recently Issued Accounting Pronouncements

A description of recently issued accounting pronouncements that may potentially impact our financial position

and results of operations is disclosed in Note 1 to our financial statements appearing elsewhere in this Annual Report.

Emerging Growth Company Status

The Jumpstart Our Business Startups Act of 2012 permits an “emerging growth company” such as us to take

advantage of an extended transition period to comply with new or revised accounting standards applicable to public
companies until those standards would otherwise apply to private companies. We have irrevocably elected to “opt out” of
this provision and, as a result, we will comply with new or revised accounting standards when they are required to be
adopted by public companies that are not emerging growth companies.

ITEM 7A.      QUANTITATIVE AND QUALITATIVE DISCLOSURES ABOUT MARKET RISK.

We are exposed to market risks in the ordinary course of our business. These risks primarily include interest rate

sensitivities and foreign currency sensitivities.

Interest Rate Sensitivity

Our exposure to market risk relates to our cash, cash equivalents and investments of $30.6 million. The primary

objective of our investment activities is to preserve principal while at the same time maximizing the income we receive
without significantly increasing risk. Some of the financial instruments in which we invest could be subject to market risk
where the interest rates may cause the value of the instruments to fluctuate. To minimize this risk, we intend to

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maintain a portfolio which may include cash, cash equivalents and short-term investment securities available-for-sale in a
variety of securities.

The securities in our investment portfolio are not leveraged and are classified as available-for-sale. These
available-for-sale securities are short-term in nature and subject to minimal interest rate risk. All investments have a fixed
interest rate and are carried at market value, which approximates cost. We do not use derivative financial instruments in our
investment portfolio. A change of 50 to 100 basis points in interest rate would result in a change of $45,000 to $0.1 million,
respectively, on the value of our investment portfolio.

We do not believe that our cash has significant risk of default or illiquidity. While we believe our cash and cash
equivalents does not contain excessive risk, we cannot provide absolute assurance that in the future our investments will
not be subject to adverse changes in market value. In addition, we maintain significant amounts of cash at one or more
financial institutions that are in excess of federally insured limits. Inflation generally affects us by increasing our cost of
labor and clinical trial costs. We do not believe that inflation has had a material effect on our results of operations during
the periods presented.

As of December 31, 2022, we had $0.6 million of outstanding short-term debt relating to our financed directors’

and officers’ insurance premium. The interest rate on this short-term loan is fixed at 2.64% per annum, and when
considering the remaining outstanding balance and the remaining term of the agreement ending in the second quarter of
2022, the loan is not subject to material interest rate risk.

Foreign Currency Sensitivity

Our primary operations are transacted in U.S. Dollars, however, certain service agreements with third parties are
denominated in currencies other than the U.S. Dollar, primarily the Euro. As such, we are subject to foreign exchange risk
and therefore, fluctuations in the value of the U.S. Dollar against the Euro may impact the amounts reported for expenses
and obligations incurred under such agreements. We do not participate in any foreign currency hedging activities and we do
not have any other derivative financial instruments. We did not recognize any significant exchange rate loss during the year
ended December 31, 2022. A hypothetical 10% change in foreign exchange rates during any of the periods presented
would not have a material impact on our financial condition or results of operations.

ITEM 8.      FINANCIAL STATEMENTS AND SUPPLEMENTARY DATA.

The information required by this item is set forth in the financial statements filed with this report and are herein

and incorporated by reference.

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Report of Independent Registered Public Accounting Firm

The Shareholders and the Board of Directors of Applied Therapeutics, Inc.

Opinion on the Financial Statements

We have audited the accompanying balance sheets of Applied Therapeutics, Inc. (the Company) as of December
31, 2022 and 2021, the related statements of operations, comprehensive income (loss), stockholders’ equity and cash flows
for  each  of  the  two  years  in  the  period  ended  December  31,  2022,  and  the  related  notes  (collectively  referred  to  as  the
“financial statements”). In our opinion, the financial statements present fairly, in all material respects, the financial position
of the Company at December 31, 2022 and 2021, and the results of its operations and its cash flows for each of the two
years in the period ended December 31, 2022, in conformity with U.S. generally accepted accounting principles.

The Company's Ability to Continue as a Going Concern

The accompanying financial statements have been prepared assuming that the Company will continue as a going
concern. As discussed in Note 1 to the financial statements, the Company has suffered recurring losses from operations,
will require additional capital to fund operations, and has stated that substantial doubt exists about the Company’s ability to
continue  as  a  going  concern.  Management's  evaluation  of  the  events  and  conditions  and  management’s  plans  regarding
these matters are also described in Note 1. The financial statements do not include any adjustments that might result from
the outcome of this uncertainty.

Basis for Opinion

These financial statements are the responsibility of the Company’s management. Our responsibility is to express
an opinion on the Company’s financial statements based on our audits. We are a public accounting firm registered with the
Public Company Accounting Oversight Board (United States) (PCAOB) and are required to be independent with respect to
the Company in accordance with the U.S. federal securities laws and the applicable rules and regulations of the Securities
and Exchange Commission and the PCAOB.

We conducted our audits in accordance with the standards of the PCAOB. Those standards require that we plan
and  perform  the  audit  to  obtain  reasonable  assurance  about  whether  the  financial  statements  are  free  of  material
misstatement, whether due to error or fraud. The Company is not required to have, nor were we engaged to perform, an
audit of its internal control over financial reporting. As part of our audits we are required to obtain an understanding of
internal  control  over  financial  reporting  but  not  for  the  purpose  of  expressing  an  opinion  on  the  effectiveness  of  the
Company’s internal control over financial reporting. Accordingly, we express no such opinion.

Our audits included performing procedures to assess the risks of material misstatement of the financial statements,
whether due to error or fraud, and performing procedures that respond to those risks. Such procedures included examining,
on  a  test  basis,  evidence  regarding  the  amounts  and  disclosures  in  the  financial  statements.  Our  audits  also  included
evaluating the accounting principles used and significant estimates made by management, as well as evaluating the overall
presentation of the financial statements. We believe that our audits provide a reasonable basis for our opinion.

/s/ Ernst & Young LLP

We have served as the Company’s auditor since 2017.

New York, New York
March 23, 2023

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Applied Therapeutics, Inc.

Balance Sheets

(in thousands except share and per share data)

ASSETS
CURRENT ASSETS:

Cash and cash equivalents
Investments
Prepaid expenses and other current assets

Total current assets
Operating lease right-of-use asset
Security deposits and leasehold improvements
TOTAL ASSETS

LIABILITIES AND STOCKHOLDERS’ EQUITY
CURRENT LIABILITIES:

Current portion of operating lease liabilities
Accounts payable
Accrued expenses and other current liabilities
Warrant liability

Total current liabilities

NONCURRENT LIABILITIES:

Noncurrent portion of operating lease liabilities
Clinical holdback - long-term portion
Total noncurrent liabilities
Total liabilities

STOCKHOLDERS’ EQUITY:

As of
December 31, 
2022

As of
December 31,
2021

$

$

$

$

$

$

16,657
13,923
6,728
37,308
857
198
38,363

477
4,534
14,756
13,657
33,424

414
464
878
34,302

53,888
26,935
7,571
88,394
1,298
200
89,892

442
9,461
16,559
—
26,462

891
—
891
27,353

Common stock, $0.0001 par value; 200,000,000 shares authorized as of
December 31, 2022 and 100,000,000 shares authorized as of December 31, 2021;
48,063,358 shares issued and outstanding as of December 31, 2022 and 26,215,514 shares
issued and outstanding as of December 31, 2021
Preferred stock, par value $0.0001; 10,000,000 shares authorized as of December 31, 2022
and December 31, 2021; 0 shares issued and outstanding as of December 31, 2022 and
December 31, 2021
Additional paid-in capital
Accumulated other comprehensive gain/(loss)
Accumulated deficit

Total stockholders' equity
TOTAL LIABILITIES AND STOCKHOLDERS’ EQUITY

5

3

-
352,828
51
(348,823)
4,061
38,363

$

-
328,958
(107)
(266,315)
62,539
89,892

$

The Notes to Financial Statements are an integral part of these statements.

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Applied Therapeutics, Inc.

Statements of Operations

(in thousands except share and per share data)

OPERATING EXPENSES:
Research and development
General and administrative
Total operating expenses
LOSS FROM OPERATIONS
OTHER INCOME (EXPENSE), NET:

Interest income
Change in fair value of warrant liabilities
Other expense

Total other income, net

Net loss
Net loss attributable to common stockholders—basic and diluted
Net loss per share attributable to common stockholders—basic and diluted
Weighted-average common stock outstanding—basic and diluted

Year Ended
December 31, 

2022

2021

$

$

55,634
27,316
82,950
(82,950)

62,570
43,048
105,618
(105,618)

685
(66)
(177)
442
(82,508) $
(82,508) $
(2.18) $

555
—
(521)
34
(105,584)
(105,584)
(4.12)
  25,598,181

$
$
$
  37,825,431

The Notes to Financial Statements are an integral part of these statements.

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Applied Therapeutics, Inc.

Statements of Comprehensive Income (Loss)

(in thousands)

Net Loss

Other comprehensive income (loss)

Unrealized gain (loss) on marketable securities

Other comprehensive gain (loss), net of tax
Comprehensive income (loss), net of tax

Year Ended
December 31, 

2022
$ (82,508)

2021
$ (105,584)

158
158
$ (82,350)

5
5
$ (105,579)

The Notes to Financial Statements are an integral part of these statements.

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Applied Therapeutics, Inc.

Statements of Stockholders’ Equity

(in thousands, except share and per share data)

Common Stock
$0.0001
Par Value

  Additional

  Accumulated Other

Paid-in
     Amount      Capital

$

2

$ 242,780

Accumulated
Deficit
(160,731)

$

$

Comprehensive
Income (Loss)

BALANCE, January 1, 2021
Issuance of common stock upon secondary public offering, net of issuance costs of
$167
Exercise of options for common stock issued under Equity Incentive Plan
Restricted Stock Unit released for common stock issued under Equity Incentive Plan
Exercise of warrants for common stock
Stock-based compensation expense
Net loss
Other comprehensive income (loss)
BALANCE, December 31, 2021

Shares
22,493,661

3,450,000
191,436
52,562
27,855
—
—
—
26,215,514

1
—
—
—
—
—
—
3

74,421
511
—
69
11,177
—
—
328,958

—
—
—
—
—
(105,584)
—
(266,315)

Total
Stockholders’
Equity

(112) $

81,939

—
—
—
—
—
—
5
(107)

74,422
511
—
69
11,177
(105,584)
5
62,539

BALANCE, January 1, 2022
Issuance of common stock, pre-funded warrants, and
common warrants sold for cash, net of issuance costs of $96
Exercise of pre-funded warrants for common stock
Exercise of options for common stock issued under Equity
Incentive Plan
Restricted Stock Units released for common issued under
Equity Incentive Plan
Stock-based compensation expense
Issuance of options in-lieu of bonus
Net loss
Other comprehensive income (loss)
BALANCE, December 31, 2022

Common Stock
$0.0001
Par Value

Shares
26,215,514

$

Amount

20,000,000
1,750,000

47,602

50,242
—
—
—
—
48,063,358

$

3

2
—

—

—
—
—
—
—
5

Additional
Paid-in
Capital

Accumulated
Deficit

Accumulated Other 
Comprehensive
Income (Loss)

Total
Stockholders’
Equity

$

328,958

$

(266,315)

$

(107)

$

62,539

12,801
1,417

49

—
9,162
441
—
—
352,828

$

—
—

—

—
—
—
(82,508)
—
(348,823)

$

$

—
—

—

—
—
—
—
158
51

$

12,803
1,417

49

—
9,162
441
(82,508)
158
4,061

The Notes to Financial Statements are an integral part of these statements.

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Applied Therapeutics, Inc.

Statements of Cash Flows

(in thousands)

OPERATING ACTIVITIES:
Net loss
Adjustments to reconcile net loss to net cash used in operating activities:

Stock-based compensation expense
Issuance of options in-lieu of bonus
Amortization of insurance premium
Amortization of operating lease right-of-use assets
Amortization of leasehold improvements
Change in operating lease liability
Change in fair value of warrant liability
Changes in operating assets and liabilities:

Financed insurance premium
Prepaid expenses
Accounts payable
Accrued expenses and other current liabilities
Other liabilities

Net cash used in operating activities

INVESTING ACTIVITIES:

Purchase of available-for-sale securities
Proceeds from sale of available-for-sale securities
Proceeds from maturities of available-for-sale securities
Net cash provided by investing activities

FINANCING ACTIVITIES:

Proceeds from June Offering issuance of shares and prefunded warrants
Proceeds from February Offering, net of cash issuance costs of $169
Proceeds from financed insurance premium
Repayments of short-term borrowings
Exercise of stock options for common stock under Equity Incentive Plan
Exercise of Warrants
Net cash provided by financing activities

NET INCREASE (DECREASE) IN CASH AND CASH EQUIVALENTS
Cash and cash equivalents at beginning of period
Cash and cash equivalents at end of period
SUPPLEMENTAL DISCLOSURE OF CASH FLOW INFORMATION:

Initial measurement of warrant liability
Conversion of warrant liability to equity for warrant exercises
Reclassification of prefunded warrant liability to equity
Unrealized gain (loss) on marketable securities

Year Ended
December 31, 

2022

2021

$

(82,508)

$

(105,584)

9,162
441
3,589
441
2
(442)
66

(3,105)
359
(4,927)
(1,635)
464
(78,093)

(64,218)
—
77,388
13,170

27,811
—
3,105
(3,273)
49
—
27,692
(37,231)
53,888
16,657

21,835
1,417
6,827
158

11,177
—
4,282
415
—
(404)
—

(4,435)
(1,654)
8,821
(3,346)
—
(90,728)

(121,589)
5,538
128,484
12,433

—
74,421
4,434
(4,718)
511
69
74,717
(3,578)
57,466
53,888

—
—
—
5

$

$
$
$
$

$

$
$
$
$

The Notes to Financial Statements are an integral part of these statements.

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Table of Contents

NOTES TO AUDITED FINANCIAL STATEMENTS

1. ORGANIZATION AND SUMMARY OF SIGNIFICANT ACCOUNTING POLICIES

Operations and Business

Applied Therapeutics, Inc. (the “Company”) is a clinical-stage biopharmaceutical company developing a pipeline
of novel product candidates against validated molecular targets in indications of high unmet medical need. In particular, the
Company is currently targeting treatments for CNS rare diseases and diabetic complications. The Company was
incorporated in Delaware on January 20, 2016 and is headquartered in New York, New York.

On January 28, 2020, the Company completed its secondary public offering (the “Secondary Public Offering”),

pursuant to which it issued and sold 2,741,489 shares of common stock at a public offering price of $45.50 per share, with
an additional 411,223 shares sold pursuant to the underwriters’ full exercise of their option to purchase additional shares.
The aggregate net proceeds received by the Company from the offering, after deducting underwriting discounts and
commissions and offering costs, were $134.1 million.

On June 4, 2020, the Company filed a shelf registration statement on Form S-3 (the “Shelf Registration
Statement”) under which the Company may, from time to time, sell securities in one or more offerings having an aggregate
offering price of up to $300.0 million. The Shelf Registration Statement was declared effective as of June 15, 2020. As of
the filing date of this Annual Report, the Company has sold 3,450,000 shares of common stock under the Shelf
Registration.

On June 12, 2020, the Company entered into an equity distribution agreement (the “Goldman Equity Distribution

Agreement”) with Goldman Sachs & Co. LLC (“Goldman”), as a sales agent to sell shares of the Company’s common
stock, from time to time, having an aggregate offering price of up to $100 million. Goldman may act as an agent on the 
Company’s behalf or purchase shares of the Company’s common stock as a principal.  As of December 31, 2021, the 
Company had not sold any shares of common stock pursuant to the Goldman Equity Distribution Agreement. This
agreement has since been terminated as of January 24, 2022.

On February 17, 2021, the Company completed an underwritten public offering (the “February Offering”) of

3,450,000 shares of common stock, including the exercise in full of the underwriters’ option to purchase 450,000 additional
shares of common stock, which option closed on February 19, 2021. The shares were offered at a price to the public
of $23.00 per share, resulting in aggregate net proceeds of approximately $74.4 million, after deducting underwriting
discounts and commissions and offering expenses.

On January 26, 2022, the Company entered into an equity distribution agreement (the “Cowen Equity Distribution

Agreement) with Cowen and Company, LLC (“Cowen”), as a sales agent, to sell shares of the Company’s common stock,
from time to time, having an aggregate offering price of up to $100.0 million. Pursuant to the Cowen Equity Distribution
Agreement shares of our common stock may be offered and sold through the sales agent in sales deemed “at-the-market”
offerings under the Securities Act of 1933, as amended, or the Securities Act. Under the Cowen Equity Distribution
Agreement, the sales agent will be entitled to compensation of up to 3% of the gross offering proceeds of all shares of our
common stock sold through it pursuant to the Cowen Equity Distribution Agreement. In connection with the sale of shares
of our common stock on our behalf, the sales agent may be deemed to be “underwriters” within the meaning of the
Securities Act, and the compensation paid to the sales agent may be deemed to be underwriting commissions or discounts.
As of December 31, 2022, the Company has not sold any shares of common stock pursuant to the Cowen Equity
Distribution Agreement.

On June 27, 2022, the Company completed an underwritten public offering (the “June Offering”) of 20,000,000

shares of common stock, par value $0.0001 per share, 10,000,000 pre-funded warrants to purchase shares of common stock
(the “Pre-Funded Warrants”), and accompanying warrants to purchase up to 30,000,000 shares of common stock (the
“Common Warrants”). The shares and accompanying Common Warrants were offered at a price to the public of $1.00 per
share and warrant, and the Pre-Funded Warrants and accompanying Common Warrants were offered at a price to the public
of $0.9999, resulting in aggregate net proceeds of approximately $27.8 million, after deducting

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underwriting discounts and commissions and offering expenses. The Pre-Funded Warrants and the Common Warrants are
immediately exercisable and will expire five years from the date of issuance. Holders may not exercise any Pre-Funded
Warrants or Common Warrants that would cause the aggregate number of shares of common stock beneficially owned by
the holder to exceed 9.99% of the Company’s outstanding common stock immediately after exercise. Holders of the Pre-
Funded Warrants and/or Common Warrants (together with affiliates) who immediately prior to June 27, 2022 beneficially
owned more than 9.99% of the Company’s outstanding common stock may not exercise any portion of their Pre-Funded
Warrants or Common Warrants if the holder (together with affiliates) would beneficially own more than 19.99% of the
Company’s outstanding common stock after exercise. The Pre-Funded Warrants and Common Warrants are subject to
adjustment in the event of certain stock dividends and distributions, stock splits, stock combinations, reclassifications or
similar events affecting the common stock and also upon any distributions for no consideration of assets to the Company’s
stockholders. In the event of certain corporate transactions, the holders of the Pre-Funded Warrants and/or Common
Warrants will be entitled to receive, upon exercise, the kind and amount of securities, cash or other property that the
holders would have received had they exercised the Pre-Funded Warrants and/or Common Warrants immediately prior to
such transaction. The Pre-Funded Warrants and Common Warrants do not entitle the holders thereof to any voting rights or
any of the other rights or privileges to which the Company’s stockholders are entitled. The Company intends to use the net
proceeds from the June Offering for general corporate purposes, which may include research and development costs,
including the conduct of clinical trials and process development and manufacturing of the Company’s product candidates,
expansion of the Company’s research and development capabilities, working capital and capital expenditures.

Liquidity and Going Concern

The Company has incurred, and expects to continue to incur, significant operating losses for the foreseeable future

as it continues to develop its drug candidates. To date, the Company has not generated any revenue, and it does not expect
to generate revenue unless and until it successfully completes development and obtains regulatory approval for one of its
product candidates.

Under ASC Topic 205-40, Presentation of Financial Statements - Going Concern, management is required at each

reporting period to evaluate whether there are conditions and events, considered in the aggregate, that raise substantial
doubt about an entity's ability to continue as a going concern within one year after the date that the financial statements are
issued. We are actively pursuing several potential financing options. While we continue to explore opportunities to raise
additional equity capital in the public markets, this has proven to be challenging in the biotech sector recently. Other
options for structured finance which we continue to explore include a PIPE (private investment in public equity), debt,
convertible debt, and synthetic royalty financing. Synthetic royalty financing, in particular, has become a favorable option
for many companies for funding ongoing clinical development in late-stage and pre-approval programs. We have engaged
an investment bank and we are specifically exploring this option in the near term. Additionally, we are in active dialogue
with several potential partners regarding business development opportunities related to one or more of our programs. There
can be no assurances that our discussions with any of the current counterparties will be successful, and the Company
expects to continue to pursue additional opportunities.

As reflected in the accompanying financial statements, the Company incurred a net loss of $82.5 million for the

year ended December 31, 2022 and has an accumulated deficit of $348.8 million as of December 31, 2022. The exclusive 
licensing agreement with Advanz  Pharma for commercialization rights to  AT-007 in Europe provides a source of  capital 
to the Company based on clinical and regulatory milestones.  We received a $10.7 million upfront payment from Advanz 
Pharma in January 2023 in conjunction with signing the agreement. If  actualization of these milestones aligns with the 
projected timelines, and product approvals are received in the timeframes expected, this source of capital may be sufficient 
to cover operating expenses through expected product approvals and potential revenues. However,  there are no guarantees 
that this will materialize timely or at all, and delays or unexpected data could disrupt this potential liquidity. Broadly, the 
Company has not yet established an ongoing source of revenues sufficient to cover its operating costs and is dependent on 
debt and equity financing to fund its operations. As of December 31, 2022, our cash, cash equivalents and marketable
securities totaled $30.6 million. Given our planned expenditures for the next twelve months, we have concluded there is
substantial doubt regarding our ability to continue as a going concern for a year beyond the date of these financial
statements. The accompanying financial statements have been prepared assuming the continuation of the Company as a
going concern.

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Risks and Uncertainties

The Company is subject to risks common to companies in the biotechnology industry, including but not limited to,
risks of failure of preclinical studies and clinical trials, the need to obtain marketing approval for any product candidate that
it may identify and develop, the need to successfully commercialize and gain market acceptance of its product candidates,
dependence on key personnel, protection of proprietary technology, compliance with government regulations, development
by competitors of technological innovations and reliance on third party manufacturers.

Use of Estimates

The preparation of financial statements in conformity with U.S. GAAP requires management to make estimates

and assumptions that affect the reported amounts of assets and liabilities, disclosure of contingent assets and liabilities and
the Company's ability to continue as a going concern as of the date of the financial statements and the reported amounts of
expenses during the reporting period. In preparing the financial statements, management used estimates in the following
areas, among others: prepaid and accrued expenses; warrant liability valuation; stock-based compensation expense; and the
evaluation of the existence of conditions and events that raise substantial doubt regarding the Company’s ability to
continue as a going concern. Actual results could differ from those estimates.

Significant Accounting Policies

Fair Value Measurements

Certain assets and liabilities are reported on a recurring basis at fair value. Fair value is defined as the exchange
price that would be received for an asset or paid to transfer a liability (an exit price) in the principal or most advantageous
market for the asset or liability in an orderly transaction between market participants on the measurement date. Valuation
techniques used to measure fair value must maximize the use of observable inputs and minimize the use of unobservable
inputs. Financial assets and liabilities carried at fair value are to be classified and disclosed in one of the following three
levels of the fair value hierarchy, of which the first two are considered observable and the last is considered unobservable:

Level 1—Quoted prices in active markets for identical assets or liabilities.

Level 2—Observable inputs (other than Level 1 quoted prices), such as quoted prices in active markets for similar

assets or liabilities, quoted prices in markets that are not active for identical or similar assets or liabilities, or other inputs
that are observable or can be corroborated by observable market data.

Level 3—Unobservable inputs that are supported by little or no market activity and that are significant to

determining the fair value of the assets or liabilities, including pricing models, discounted cash flow methodologies and
similar techniques.

Cash and Cash Equivalents

The Company considers all short-term, highly liquid investments, with an original maturity of three months or

less, to be cash equivalents. The Company maintains its cash in bank deposit accounts which, at times, may exceed
federally insured limits. The Company has not experienced any losses in these accounts and does not believe it is exposed
to any significant credit risk on cash and cash equivalents.

Investments

The Company has investments in marketable debt securities. The Company determines the appropriate

classification of its investments at the date of purchase and reevaluates the classifications at the balance sheet date.
Marketable debt securities with maturities of 12 months or less are classified as short-term. Marketable debt securities with
maturities greater than 12 months are classified as long-term. The Company’s marketable securities are accounted for as
available for sale (“AFS”). AFS securities are reported at fair value. Unrealized gains and losses, after applicable

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income taxes, are reported in accumulated other comprehensive income/(loss). Realized gains or losses on the sale of
marketable securities are determined using the specific identification method and are recorded as a component of other
income (expense), net.

The Company conducts an other-than-temporary impairment (“OTTI”) analysis on a quarterly basis or more often
if a potential loss-triggering event occurs. The Company considers factors such as the duration, severity and the reason for
the decline in value, the potential recovery period and whether the Company intends to sell. For AFS securities, the
Company also considers whether (i) it is more likely than not that the Company will be required to sell the debt securities
before recovery of their amortized cost basis and (ii) the amortized cost basis cannot be recovered as a result of credit
losses.

Leases

At the inception of an arrangement, the Company determines if an arrangement is, or contains, a lease based on the
unique  facts  and  circumstances  present  in  that  arrangement.  Lease  classification,  recognition,  and  measurement  are  then
determined at the lease commencement date. For arrangements that contain a lease the Company (i) identifies lease and
non-lease components, (ii) determines the consideration in the contract, (iii) determines whether the lease is an operating or
financing  lease;  and  (iv)  recognizes  lease  right-of-use  (“ROU”)  assets  and  liabilities.  Lease  liabilities  and  their
corresponding ROU assets are recorded based on the present value of lease payments over the expected lease term. The
interest rate implicit in lease contracts is typically not readily determinable and as such, the Company uses its incremental
borrowing  rate  based  on  the  information  available  at  the  lease  commencement  date,  which  represents  an  internally
developed rate that would be incurred to borrow, on a collateralized basis, over a similar term, an amount equal to the lease
payments in a similar economic environment.

Most leases include options to renew and, or, terminate the lease, which can impact the lease term. The exercise of
these options is at the Company’s discretion and the Company does not include any of these options within the expected
lease term as the Company is not reasonably certain it will exercise these options. The Company has elected to combine
lease  components  (for  example  fixed  payments  including  rent)  with  non-lease  components  (for  example,  non-dedicated
parking and common-area maintenance costs) on our real estate asset classes.

Fixed, or in substance fixed, lease payments on operating leases are recognized over the expected term of the lease
on  a  straight-line  basis.  Fixed  lease  expense  on  operating  leases  is  recognized  within  operating  expenses  within  the
statements of operations. The Company has operating leases for our corporate offices. The Company has elected the short-
term lease exemption and, therefore, do not recognize a ROU asset or corresponding liability for lease arrangements with
an  original  term  of  12  months  or  less.  Leasehold  improvements  and  assets  under  financing  lease  arrangements  are
amortized  over  the  lesser  of  the  asset’s  estimated  useful  life  or  the  term  of  the  respective  lease.  Maintenance  costs  are
expensed as incurred.

Operating leases are included in operating lease right-of-use asset, current portion of operating lease liabilities, and

noncurrent portion of operating lease liabilities in the balance sheet as of December 31, 2022 and 2021.

Clinical hold-back, long-term

As part of the regulatory approval process for taking its products to market, the Company enters into certain
Clinical Trial Agreements (CTAs) which include, among other things, the compensation and payment schedule the
participating medical institutions and physicians will receive for all costs in connection with the clinical trial (or study)
under the terms of the CTA. As individual patients are enrolled in the study by the participating medical institution or
physician, the Company pays certain per study fees according to the CTA for the duration of the trial. As invoices are
received by the Company from the medical institution or physician, the Company retains an agreed upon percentage of
total invoiced costs, generally ranging between 5% - 10%, that is withheld from payment until the end of the study.

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These retained amounts are recorded as clinical holdback, a liability, on the accompanying balance sheets, and all

expenses incurred in connection with these CTA activities are expensed as services are provided, which are included as
research and development expenses on the accompanying statements of operations.

The following table shows the activity within the clinical holdback liability accounts for the year ended December

31, 2022:

(in thousands)
Balance as of December 31,2021
Clinical holdback retained
Clinical holdback paid
Balance as of December 31,2022
Less: clinical holdback current portion
Clinical holdback - long-term portion

$

$

$

—
464
—
464
—
464

There was no clinical holdback during the year ended December 31, 2021.

Deferred Offering Costs

The Company capitalizes certain legal, professional accounting and other third party fees that are directly associated
with in-process equity financings as deferred offering costs until such financings are consummated. After consummation of
the equity financing, these costs are recorded in the statement of stockholders’ (deficit) equity as a reduction of proceeds
generated as a result of the offering. Should a planned equity financing be abandoned, the deferred offering costs would be
expensed immediately as a charge to operating expenses in the statement of operations.

As of December 31, 2022 and 2021, the Company did not have any deferred offering costs recorded in prepaid and

other current assets.

Research and Development

The Company expenses all costs incurred in performing research and development activities. Research and
development expenses include salaries and other related costs, materials and supplies, preclinical expenses, manufacturing
expenses, contract services and other outside expenses. As part of the process of preparing the financial statements, the
Company is required to estimate their accrued research and development expenses. The Company makes estimates of the
accrued expenses as of each balance sheet date in the financial statements based on facts and circumstances known at that
time. In addition, there may be instances in which payments made to the Company’s vendors will exceed the level of
services provided and result in a prepayment of the expense in which case such amounts are reflected as prepaid expenses
and other current assets. In accruing service fees, the Company estimates the time period over which services will be
performed and the level of effort to be expended in each period. If the actual timing of the performance of services or the
level of effort varies from the estimate, the Company adjusts the accrual or the amount of prepaid expenses accordingly.
Nonrefundable advance payments for goods or services to be received in the future for use in research and development
activities are deferred and capitalized in prepaid expenses and other current assets. The capitalized amounts are expensed
as the related goods are delivered or the services are performed.

Research and development costs also include costs incurred in connection with certain licensing arrangements.
Before a compound receives regulatory approval, the Company records upfront and milestone payments made to third
parties under licensing arrangements as expense. Upfront payments are recorded when incurred, and milestone payments
are recorded when the specific milestone has been achieved. Once a compound receives regulatory approval, the Company
will record any milestone payments in identifiable intangible assets, less accumulated amortization and, unless the asset is
determined to have an indefinite life, the Company will amortize the payments on a straight-line basis over the remaining
agreement term or the expected product life cycle, whichever is shorter.

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Table of Contents

General and Administrative

General and administrative expenses consist primarily of salaries and other related costs, including stock-based

compensation, for personnel in the Company’s executive and finance functions. General and administrative expenses also
include professional fees for legal, accounting, auditing, tax and consulting services; travel expenses; and facility-related
expenses, which include allocated expenses for rent and maintenance of facilities and other operating costs.

Commercial expenses consist of payroll expense for commercial personnel, as well as marketing, market research,

market access, and other focused investments to support launch of drug candidates, generate evidence of commercial
potential and value proposition, and maximize potential business development deal leverage. Commercial expenses are
included in general and administrative expenses.

Stock-Based Compensation

The Company accounts for its stock-based compensation as expense in the statements of operations based on the
awards’ grant date fair values. The Company accounts for forfeitures as they occur by reversing any expense recognized
for unvested awards.

The Company estimates the fair value of options granted using the Black-Scholes option pricing model. The Black-

Scholes option pricing model requires inputs based on certain subjective assumptions, including (a) the expected stock
price volatility, (b) the calculation of expected term of the award, (c) the risk-free interest rate and (d) expected dividends.
Due to the lack of a public market for the Company’s common stock and a lack of company-specific historical and implied
volatility data, the Company has based its estimate of expected volatility on the historical volatility of a group of similar
companies that are publicly traded. The historical volatility is calculated based on a period of time commensurate with the
expected term assumption. The computation of expected volatility is based on the historical volatility of a representative
group of companies with similar characteristics to the Company, including stage of product development and life science
industry focus. The Company uses the simplified method as allowed by the Securities and Exchange Commission (“SEC”)
Staff Accounting Bulletin (“SAB”) No. 107, Share-Based Payment, to calculate the expected term for options granted to
employees as it does not have sufficient historical exercise data to provide a reasonable basis upon which to estimate the
expected term. The risk-free interest rate is based on a treasury instrument whose term is consistent with the expected term
of the stock options. The expected dividend yield is assumed to be zero as the Company has never paid dividends and has
no current plans to pay any dividends on its common stock.

The fair value of stock-based payments is recognized as expense over the requisite service period which is generally

the vesting period.

Stock-Based Compensation–Restricted Stock Units

The Company accounts for restricted stock units in accordance with the authoritative guidance for stock-based

compensation. The fair value of restricted stock units is measured at the grant date based on the closing market price of the
Company’s common stock on the date of grant, and is recognized as expense on a straight-line basis over the period of
vesting. Forfeitures are recognized as a reduction of stock-based compensation expense as they occur.

Income Taxes

The Company uses the asset and liability method of accounting for deferred income taxes. Under this method,
deferred tax assets and liabilities are recognized for the expected future tax consequences of temporary differences between
the carrying amounts and the tax basis of assets and liabilities at currently enacted tax rates. These temporary differences
primarily relate to net operating loss carryforwards available to offset future taxable income. Valuation allowances are
established, if necessary, to reduce a deferred tax asset to the amount that will more likely than not be realized.

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The Company recognizes tax liabilities from an uncertain tax position only if it is more likely than not that the tax

position will not be sustained upon examination by the taxing authorities, based on the technical merits of the tax position.
There are no uncertain tax positions that have been recognized in the accompanying financial statements. The Company is
required to file tax returns in the U.S. federal jurisdiction and in the states of New York, California, Massachusetts, New
Jersey, and New York City. The Company’s policy is to recognize interest and penalties related to uncertain tax benefits, if
any, as part of income tax expense. No such interest and penalties have been accrued as of December 31, 2022 and 2021.

In December 2019, the FASB issued ASU 2019-12, Income Taxes: Simplifying the Accounting for Income
Taxes. The new standard intended to simplify the accounting for income taxes by eliminating certain exceptions related to
the approach for intraperiod tax allocation, the methodology for calculating income taxes in an interim period and the
recognition of deferred tax liabilities for outside basis differences. The new guidance also simplifies aspects of the
accounting for franchise taxes and enacted changes in tax laws or rates and clarifies the accounting for transactions that
result in a step-up in the tax basis of goodwill. The standard is effective for annual periods beginning after December 15,
2020 and interim periods within, with early adoption permitted. Adoption of the standard requires certain changes to
primarily be made prospectively, with some changes to be made retrospectively. The Company adopted the amendment on
January 1, 2021, with no impact to the financial statements.

Net Loss per Share

Basic net loss per share is calculated by dividing net loss available to common stockholders by the weighted-average
common stock outstanding. Diluted net loss per share is calculated similarly, except that it includes the dilutive effect of the
assumed exercise of securities, including outstanding warrants and the effect of shares issuable under the Company’s stock-
based compensation plan, if such effect is dilutive.

Segment Information

Operating segments are defined as components of an enterprise for which separate discrete information is available

for evaluation by the chief operating decision-maker in deciding how to allocate resources and assess performance. The
Company and the Company’s chief operating decision-maker, the Company’s chief executive officer, views the Company’s
operations and manages its business as a single operating segment, which is the business of discovering and developing its
product candidates.

Recent Accounting Pronouncements

Any recent pronouncements issued by the FASB or other authoritative standards groups with future effective dates

are either not applicable or are not expected to be significant to the financial statements of the Company.

2. LICENSE AGREEMENT

Columbia University

In October 2016, the Company entered into a license agreement (the “2016 Columbia Agreement”) with the

Trustees of Columbia University (“Columbia University”) to obtain an exclusive royalty-bearing sublicensable license in
respect to certain patents. As part of the consideration for entering into the 2016 Columbia Agreement, the Company issued
to Columbia University shares equal to 5% of its outstanding common stock on a fully diluted basis at the time of issue.
The common stock had a fair value of $0.5 million at the time of issuance. The Company will be required to make further
payments to Columbia University of up to an aggregate of $1.3 million for the achievement of specified development and
regulatory milestones, and up to an aggregate of $1.0 million for the achievement of a specified level of aggregate annual
net sales, in each case in connection with products covered by the 2016 Columbia Agreement. The Company will also be
required to pay tiered royalties to Columbia University in the low- to mid-single digit percentages on the Company’s, its
affiliates’ and its sublicensees’ net sales of licensed products, subject to specified offsets and reductions. In addition, the
Company is required to make specified annual minimum royalty payments to Columbia

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Table of Contents

University, which is contingent upon the approval of the licensed products, in the mid-six figures beginning on the
10th anniversary of the effective date of the 2016 Columbia Agreement. When we grant sublicenses under the 2016
Columbia Agreement we are required to pay Columbia University a portion of the net sublicensing revenue received from
such third parties, at percentages between 10% and 20%, depending on the stage of development at the time such revenue
is received from such third parties. The Advanz Agreement includes a sublicense under the 2016 Columbia Agreement.

The 2016 Columbia Agreement will terminate upon the expiration of all the Company’s royalty payment

obligations in all countries. The Company may terminate the 2016 Columbia Agreement for convenience upon 90 days’
written notice to Columbia University. At its election, Columbia University may terminate the 2016 Columbia Agreement,
or convert the licenses granted to the Company into non-exclusive, non-sublicensable licenses, in the case of (a) the
Company’s uncured material breach upon 30 days’ written notice (which shall be extended to 90 days if the Company is
diligently attempting to cure such material breach), (b) the Company’s failure to achieve the specified development and
funding milestone events, or (c) the Company’s insolvency.

In January 2019, the Company entered into a second license agreement with Columbia University (the “2019

Columbia Agreement”). Pursuant to the 2019 Columbia Agreement, Columbia University granted the Company a royalty-
bearing, sublicensable license that is exclusive with respect to certain patents, and non-exclusive with respect to certain
know-how, in each case to develop, manufacture and commercialize PI3k inhibitor products. The license grant is
worldwide. Under the 2019 Columbia Agreement, the Company is obligated to use commercially reasonable efforts to
research, discover, develop and market licensed products for commercial sale in the licensed territory, and to comply with
certain obligations to meet specified development and funding milestones within defined time periods. Columbia
University retains the right to conduct, and grant third parties the right to conduct, non-clinical academic research using the
licensed technology; provided that such research is not funded by a commercial entity or for-profit entity or results in rights
granted to a commercial or for-profit entity. As consideration for entering into the 2019 Columbia Agreement, the
Company made a nominal upfront payment to Columbia University. The Company will be required to make further
payments to Columbia University of up to an aggregate of $1.3 million for the achievement of specified development and
regulatory milestones, and up to an aggregate of $1.0 million for the achievement of a specified level of aggregate annual
net sales, in each case in connection with products covered by the 2019 Columbia Agreement. The Company will also be
required to pay tiered royalties to Columbia University in the low- to mid-single digit percentages on the Company’s, its
affiliates’ and its sublicensees’ net sales of licensed products, subject to specified offsets and reductions. In addition, the
Company is required to make specified annual minimum royalty payments to Columbia University, which is contingent
upon the approval of the licensed products, in the mid-six figures beginning on the tenth anniversary of the effective date of
the 2019 Columbia Agreement.

In July 2022, following regulatory changes impacting development of the class of PI3k inhibitors and the 

Company’s decision to discontinue its early stage preclinical PI3k program, the Company and Columbia entered into an 
agreement terminating the 2019 Columbia Agreement (the “2022 Columbia Termination Agreement”) as of July 25, 2022.   
Under the terms of the 2022 Columbia Termination Agreement, the Company assigned certain regulatory documents 
regarding the preclinical PI3k inhibitor AT-104 to Columbia and granted Columbia a non-exclusive royalty free license 
(with rights to sublicense any future Columbia licensee) under certain know-how, technical information and data relating to 
AT-104 that was developed by the Company during the term of the 2019 Columbia Agreement.

In March 2019, and in connection with the 2016 Columbia Agreement, the Company entered into a research 

services agreement (the “2019 Columbia Research Agreement”) with Columbia University with the purpose of analyzing 
structural and functional changes in brain tissue in an animal model of Galactosemia, and the effects of certain compounds 
whose intellectual property rights were licensed to the Company as part of the 2016 Columbia Agreement on any such 
structural and functional changes.  The 2019 Columbia Research Agreement had a term of 12 months from its effective 
date and expired in accordance with its terms.   

On October 3, 2019, and in connection with the 2019 Columbia Agreement, the Company entered into a research

services agreement (the “PI3k Columbia Research Agreement” and collectively with the 2016 Columbia Agreement, 2019
Columbia Agreement and 2019 Columbia Research Agreement, the “Columbia Agreements”) with Columbia

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Table of Contents

University with the purpose of analyzing PI3k inhibitors for the treatment of lymphoid malignancies. The PI3k Columbia
Research Agreement had a term of 18 months from its effective date and expired in accordance with its terms.

During the years ended December 31, 2022 and 2021, the Company recorded $0 and $0 in research and

development expense, respectively, and $0.2 million and $0.2 million, respectively, in general and administrative expense
related to the Columbia Agreements. In aggregate, the Company has incurred $2.7 million in expense from the execution
of the Columbia Agreements through December 31, 2022.

As of December 31, 2022, the Company had $0.1 million due to Columbia University included in accrued expenses

and $0 included in accounts payable. As of December 31, 2021, the Company had $12,000 due to Columbia University
included in accrued expenses and $0.1 million included in accounts payable.

University of Miami

2020 Miami License Agreement

On October 28, 2020, the Company entered into a license agreement with the University of Miami (the “2020

Miami License Agreement”) relating to certain technology that is co-owned by the University of Miami (UM), the
University of Rochester (UR) and University College London (UCL). UM was granted an exclusive agency from UR and
UCL to license each of their rights in the technology. Pursuant to the 2020 Miami License Agreement, UM, on behalf of
itself and UR and UCL, granted the Company a royalty-bearing, sublicensable license that is exclusive with respect to
certain patent applications and patents that may grant from the applications, and non-exclusive with respect to certain
know-how, in each case to research, develop, make, have made, use, sell and import products for use in treating and/or
detecting certain inherited neuropathies, in particular those caused by mutation in the sorbitol dehydrogenase (SORD)
gene. The license grant is worldwide. Under the 2020 Miami License Agreement, the Company is obligated to use
commercially reasonable efforts to develop, manufacture, market and sell licensed products in the licensed territory, and to
comply with certain obligations to meet specified development milestones within defined time periods. UM retains for
itself, UR, and UCL the right to use the licensed patent rights and licensed technology for their internal non-commercial
educational, research and clinical patient care purposes, including in sponsored research and collaboration with commercial
entities.

Under the terms of the 2020 Miami License Agreement, the Company was obligated to pay UM an up-front non-
refundable license fee of $1.1 million, and a second non-refundable license fee of $0.5 million due on the first anniversary
of the date of the license. The Company will be required to make further payments to UM of up to an aggregate $2.2
million for the achievement of specified patenting and development milestones, and up to an aggregate of $4.1 million for
achievement of late stage regulatory milestones. The Company will also be required to pay royalties ranging from 0.88% -
5% on the Company’s, the Company’s affiliates’ and the Company’s sublicensees’ net sales of licensed products. When the
Company sublicenses the rights granted under the 2020 Miami License Agreement to one or more third parties, the
Company will be required to pay to UM a portion of the non-royalty sublicensing revenue received from such third parties
ranging from 15% – 25%. The Advanz Agreement includes a sublicense under the 2020 Miami License Agreement.

The  2020  Miami  License  Agreement  terminates  upon  the  expiration  of  all  issued  patents  and  filed  patent
applications  or  10  years  after  the  first  commercial  sale  of  the  last  product  or  process  for  which  a  royalty  is  due,  unless
earlier terminated. In addition, the 2020 Miami License Agreement may be terminated by the Company at any time upon
60  days  prior  written  notice  to  UM,  and  may  be  terminated  by  either  the  Company  or  UM  upon  material  breach  of  an
obligation if action to cure the breach is not initiated within 60 days of receipt of written notice.

The Company recorded $0.1 million and $0 in research and development expense and general and administrative
expense, respectively, during the year-ended December 31, 2022. As of December 31, 2022, the Company had $0.3 million
in accrued expenses.

The Company recorded $0.03 million and $0 in research and development expense and general and administrative
expense, respectively, during the year-ended December 31, 2021. As of December 31, 2021, the Company had $0.3 million
in accrued expenses.

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Table of Contents

2020 Miami Option Agreement

On October 28, 2020, the Company entered into an option agreement with the University of Miami (the “2020

Miami Option Agreement”) concerning certain research activities and technology relating to SORD neuropathy that may
be pursued and developed by UM. Under the 2020 Miami Option Agreement, if UM conducts such research activities, then
UM is obligated to grant us certain option rights to access and use the research results and to obtain licenses to any
associated patent rights upon us making specified payments to UM within specified time limits. If the Company elects to
obtain option rights the Company will be required to make payments to UM in the low-six figures to the low-seven figures,
depending upon the rights the Company elects to obtain, and the Company will be obligated to make certain milestone
payments in the high-six figures to mid-seven figures if UM conducts and completes certain research activities within
specified time periods and the Company elects to receive rights to use the results of that research.

2020 Miami Sponsored Research Agreement

On December 14, 2020, the Company entered into a research agreement with the University of Miami (the “2020

Miami Research Agreement”), under which the University of Miami will conduct a research study relating to SORD
neuropathy and deliver a final report on the study to the Company. The term of the research agreement was from December
14, 2020 through December 30, 2021, and was extended through August 31, 2022. The total consideration for the 2020
Miami Research Agreement was $0.3 million.

During the years ended December 31, 2022 and 2021, the Company recorded $48,000 and $0.2 million in research
and development expenses, respectively, in relation to the 2020 Miami Research Agreement. As of December 31, 2022 and
2021, the Company had $1.0 million and $0.2 million, respectively, in accrued expenses.

Bayh-Dole Act

Some of the intellectual property rights the Company has licensed, including certain rights licensed in the

agreements described above, may have been generated through the use of U.S. government funding. As a result, the U.S.
government may have certain rights to intellectual property embodied in the Company’s current or future product
candidates under the Bayh-Dole Act of 1980, or Bayh-Dole Act, including the grant to the government of a non-exclusive,
worldwide, freedom to operate license under any patents, and the requirement, absent a waiver, to manufacture products
substantially in the United States.  To the extent any of the Company’s current or future intellectual property is generated
through the use of U.S. government funding, the provisions of the Bayh-Dole Act may similarly apply.

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Table of Contents

3. FAIR VALUE MEASUREMENTS

The following tables summarize, as of December 31, 2022 and 2021, the Company's financial assets and liabilities

that are measured at fair value on a recurring basis, according to the fair value hierarchy described in the significant
accounting policies section.

(in thousands)
Cash
Money market funds

Total cash and cash equivalents

U.S. government agency debt securities

Total marketable securities
Total financial assets measured at fair value on
a recurring basis

Warrant liabilities - Common Warrants

Level 1

As of December 31, 2022

Level 2

Level 3

Total

$

$

1,337
15,320
$ 16,657

— $
—
— $

$
— 13,923
— $ 13,923

$

1,337
— $
—
15,320
— $ 16,657
—
13,923
— $ 13,923

$ 16,657
—

$ 13,923

— 13,657

— $ 30,580
13,657

$

$

Total financial liabilities measured at fair value
on a recurring basis

$

— $

— $ 13,657

$ 13,657

As of December 31, 2021

(in thousands)
Cash
Money market funds

Total cash and cash equivalents

U.S. government agency debt securities

Total marketable securities
Total financial assets measured at fair value on
a recurring basis

Level 1
$ 12,671
41,217
$ 53,888

Level 2

$

Level 3
— $ — $
—
— $ — $

—

$
— 26,935
— $ 26,935

—
$ — $

$

Total
12,671
41,217
53,888
26,935
26,935

$ 53,888

$ 26,935

$ — $

80,823

Investments in certificate of deposits, corporate bonds, and U.S. government agency debt securities have been

classified as Level 2 as they are valued using quoted prices in less active markets or other directly or indirectly observable
inputs. Fair values of corporate bonds and U.S. government agency debt securities were derived from a consensus or
weighted average price based on input of market prices from multiple sources at each reporting period. With regard to
commercial paper, all of the securities had high credit ratings and one year or less to maturity; therefore, fair value was
derived from accretion of purchase price to face value over the term of maturity or quoted market prices for similar
instruments if available. During the period ended December 31, 2022 and 2021, there were no transfers of financial assets
between Level 1 and Level 2.

On June 27, 2022 the Company issued Common Warrants exercisable for 30,000,000 shares of common stock and
Pre-Funded Warrants exercisable for 10,000,000 shares of common stock in connection with the June Offering (see note 1
and note 8 for more information on the June Offering). The Common Warrants were accounted for as liabilities under ASC
815-40,  Derivatives  and  Hedging,  Contracts  in  Entity’s  Own  Equity  (“ASC  815-40”),  as  these  warrants  provide  for  a
settlement provision that does not meet the requirements of the indexation guidance under ASC 815-40. The Pre-Funded
Warrants  were  initially  recorded  at  fair  value  as  a  liability  as  the  Company  could  be  required  to  settle  the  Pre-Funded
Warrants  in  cash  under  certain  circumstances.  In  December  2022,  the  Company  amended  the  Pre-Funded  Warrants  to
remove the potential requirement that they could be settled in cash under certain circumstances.  Upon the amendment to
the  Pre-Funded  Warrants,  the  Pre-funded  Warrants  liability  was  reclassified  to  equity,  using  their  fair  value  as  of  the
amendment date.

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Table of Contents

These Common Warrant liabilities were measured at fair value at inception and are then subsequently measured
on a recurring basis, with changes in fair value recognized in other income (expense) within the Company’s statement of
operations.

The Company uses a Black-Scholes option pricing model to estimate the fair value of the Common and Pre-

Funded Warrants, which utilizes certain unobservable inputs and is therefore considered a Level 3 fair value measurement.
Certain inputs used in this Black-Scholes pricing model may fluctuate in future periods based upon factors that are outside
of the Company’s control, including a potential change in control outside of the Company’s control. A significant change in
one or more of these inputs used in the calculation of the fair value may cause a significant change to the fair value of the
Company’s warrant liabilities, which could also result in material non-cash gains or losses being reported in the Company’s
consolidated statement of operations.

The Common and Pre-Funded Warrants were initially valued and remeasured using a Black-Scholes option

pricing model with a range of assumptions as follows:

Expected term (in years)
Volatility
Risk-free interest rate
Dividend yield

3.7  
91.53 %
4.11 %
0.00 %

The Company utilized a probability-weighted approach that considered the probability of a change in control at

the Company in the Black-Scholes option pricing model, whereby a 10% probability of change in control was used for
each of the five years in the term of the agreements.

The following table provides a roll forward of the aggregate fair values of the Company’s warrant liability, for

which fair value is determined using Level 3 inputs (in thousands):

Balance as of January 1, 2022

Initial fair value of Warrant Liability
Warrants exercised
Change in fair value
Reclassification of pre-funded warrant liability to equity

Balance as of December 31, 2022

Warrant Liability

Common
Warrant

Pre-Funded
Warrant

$

— $
13,734  
—
(77)  

$

13,657 $

—
8,101
(1,417)
143
(6,827)
—

The inputs utilized by management to value the warrant liability for Common and Pre-Funded Warrants are highly

subjective. The assumptions used in calculating the fair value of the warrant liability for Common and Pre-Funded
Warrants represent the Company’s best estimates, but these estimates involve inherent uncertainties and the application of
management judgment. As a result, if factors change and the Company uses different assumptions, the fair value of the
warrant liability for Common Warrants may be materially different in the future.

4. INVESTMENTS

Marketable Securities

Marketable securities, which the Company classifies as available-for-sale securities, primarily consist of high

quality commercial paper, corporate bonds, and U.S. government debt obligations. Marketable securities with remaining
effective maturities of twelve months or less from the balance sheet date are classified as short-term; otherwise, they are
classified as long-term on the balance sheets.

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Table of Contents

The following tables provide the Company’s marketable securities by security type (in thousands):

As of December 31, 2022

Gross

Gross
    Unrealized    Unrealized     Estimated     
Losses

Fair Value

Gains

Cost

As of December 31, 2021

Gross

Gross

Cost

    Unrealized    Unrealized     Estimated
Fair Value

Losses

Gains

$13,873
$13,873

$
$

50
50

$ — $13,923
$ — $13,923

$27,042
$27,042

$
$

1
1

$
$

(108) $26,935
(108) $26,935

(in thousands)
US
government
agency debt
security

Total

As of December 31, 2022, the Company’s investment portfolio reported no unrealized loss.  Based on its 

evaluations, the Company determined that a credit loss allowance is not required since the decline was not related to 
underlying credit issues of the counterparties. The counterparties to these investments have high credit quality with 
investment grade ratings of at least AA+ or above, along with a history of no defaults. No single investment in the portfolio 
had an individually material unrealized loss and in the aggregate. In addition, the Company does not intend to sell these 
investments and it is not more likely than not that the Company will be required to sell these investments before recovery 
of their amortized cost bases. Accordingly, based on the foregoing evaluation, the Company did not record any credit losses 
during the year ended December 31, 2022 and 2021. Unrealized gains are also reflected, net of tax, as other comprehensive 
income (loss) in the Statements of Comprehensive Loss.

Contractual maturities of the Company’s marketable securities are summarized as follows (in thousands):

Cost

(in thousands)
Due in one
year or less $ 13,873
Due in one
through
two years

—
Total $ 13,873

As of December 31, 2022

Gross

Gross
Unrealized Unrealized     Estimated

     Gains

     Losses

     Fair Value     

Cost

As of December 31, 2021

Gross

Gross
Unrealized Unrealized     Estimated
     Fair Value

     Losses

     Gains

$

50

$ — $ 13,923

$ 27,042

$

1

$

(108) $ 26,935

—
—
—
50    $ — $ 13,923

—
$ 27,042

$

—
1    $

—

—
(108) $ 26,935

$

At December 31, 2022, the Company had $50,000 of gross unrealized gains and $0 of gross unrealized losses

primarily due to fluctuations in the fair value of certain U.S. government agency debt securities.

During the year ended December 31, 2022, the Company recorded gross realized losses of $0.2 million and gross

realized gains of $16,000 from the redemption of marketable securities.

The unrealized losses and fair values of available-for-sale securities that have been in an unrealized loss position

for a period of less than and greater than 12 months as of December 31, 2022 are as follows:

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(in thousands)
US government agency
debt security
Total

Securities in an
unrealized loss position
less than 12 months

As of December 31, 2022
Securities in an
unrealized loss position
greater than 12 months
Unrealized     Estimated     Unrealized     Estimated     Unrealized     Estimated
Fair Value

Fair Value

Fair Value

Losses

Losses

Losses

Total

$ — $ — $ — $ — $ — $ —
$ — $ — $ — $ — $ — $ —

The unrealized losses and fair values of available-for-sale securities that have been in an unrealized loss position

for a period of less than and greater than 12 months as of December 31, 2021 are as follows:

Securities in an
unrealized loss position
less than 12 months

As of December 31, 2021
Securities in an
unrealized loss position
greater than 12 months
Unrealized     Estimated     Unrealized     Estimated     Unrealized     Estimated
Fair Value

Fair Value

Fair Value

Losses

Losses

Losses

Total

$
$

(108) $ 17,696
(108) $ 17,696

$ — $ — $
$ — $ — $

(108) $ 17,696
(108) $ 17,696

(in thousands)
US government agency
debt security
Total

5. PREPAID EXPENSE AND OTHER CURRENT ASSETS

Prepaid expenses and other current assets consisted of the following (in thousands):

(in thousands)
Prepaid research and development expenses
Insurance premium asset
Prepaid rent expenses
Prepaid insurance expenses
Prepaid commercial and patient advocacy
Research and development tax credit receivable
Interest receivable
Other prepaid expenses and current assets
Total prepaid expenses & other current assets

F-20

    December 31,     December 31,

2022

2021

$

$

4,272
1,131
99
71
206
252
23
674
6,728

$

$

4,483
1,616
117
105
254
502
23
471
7,571

 
 
 
 
 
 
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6. ACCRUED EXPENSE AND OTHER CURRENT LIABILITIES

Accrued expenses and other current liabilities consisted of the following (in thousands):

(in thousands)
Accrued pre-clinical and clinical expenses
Short-term insurance financing note
Accrued professional fees
Accrued compensation and benefits
Accrued commercial expenses
Accrued patent expenses
Other
Total accrued expenses & other current liabilities

    December 31,     December 31,

2022

8,877
622
1,218
2,301
896
361
481
14,756

$

$

2021

9,912
789
419
2,779
1,394
279
987
16,559

$

$

7. STOCK-BASED COMPENSATION

Equity Incentive Plans

In May 2019, the Company's board of directors (the "Board") adopted its 2019 Equity Incentive Plan ("2019
Plan"), which was subsequently approved by its stockholders and became effective on May 13, 2019. As a result, no
additional awards under the Company's 2016 Equity Incentive Plan, as amended (the "2016 Plan") will be granted and all
outstanding stock awards granted under the 2016 Plan that are repurchased, forfeited, expired or are cancelled will become
available for grant under the 2019 Plan in accordance with its terms. The 2016 Plan will continue to govern outstanding
equity awards granted thereunder.

The 2019 Plan provides for the issuance of incentive stock options ("ISOs") to employees, and for the grant of 
nonstatutory stock options, stock appreciation rights, restricted stock awards, restricted stock unit awards, performance 
stock awards, performance cash awards and other forms of stock awards to the Company's employees, officers and 
directors, as well as non- employees, consultants and affiliates to the Company. Under the terms of the 2019 Plan, stock 
options may not be granted at an exercise price less than fair market value of the Company's common stock on the date of 
the grant.  The 2019 Plan is administered by the Compensation Committee of the Company's Board.

Initially, subject to adjustments as provided in the 2019 Plan, the maximum number of the Company's common
stock that may be issued under the 2019 Plan is 4,530,000 shares, which is the sum of (i) 1,618,841 new shares, plus (ii)
the number of shares (not to exceed 2,911,159 shares) that remained available for the issuance of awards under the 2016
Plan, at the time the 2019 Plan became effective, and (iii) any shares subject to outstanding stock options or other stock
awards granted under the 2016 Plan that are forfeited, expired, or reacquired. The 2019 Plan provides that the number of
shares reserved and available for issuance under the 2019 Plan will automatically increase each January 1, beginning on
January 1, 2020, by 5% of the outstanding number of shares of common stock on the immediately preceding December 31
or such lesser number of shares as determined by the Board. Subject to certain changes in capitalization of the Company,
the aggregate maximum number of shares of common stock that may be issued pursuant to the exercise of ISOs shall be
equal to 13,000,000 shares of common stock. Stock options awarded under the 2019 Plan expire 10 years after grant and
typically vest over four years.

On August 2, 2022, the Board took action in accordance with its authority under the terms of the 2019 Plan to

reset the per-share exercise price of all stock options previously granted under the 2019 Plan to $1.05 per share (the
"Options Repricing"), which is equal to the closing price of a share of the Company’s common stock on August 1, 2022.
The Options Repricing was deemed to be a Type I modification event under ASC 718, Compensation-Stock Compensation.
No other terms of the repriced stock options were modified, and the repriced stock options will continue to vest according
to their original vesting schedules and will retain their original expiration dates. As a result of the

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Options Repricing, 1,797,517 vested and 1,380,917 unvested stock options outstanding as of August 2, 2022, with original
exercise prices ranging from $1.22 to $49.60, were repriced. The Options Repricing resulted in incremental
stock-based compensation expense of $1.4 million, of which $0.9 million related to vested stock option awards and was
expensed on the repricing date, and $0.5 million of which related to unvested stock option awards and is being amortized
on a ratable basis over the remaining weighted-average vesting period of those awards being approximately 2.4 years.

As of December 31, 2022, there were 1,096,493 shares of common stock available for issuance under the 2019
Plan. On January 1, 2023, there were 2,403,167 shares that became issuable for future grants subject to the adjustments
provided in the 2019 Plan.

Stock-Based Compensation Expense

Total stock-based compensation expense recorded for employees, directors and non-employees (in thousands):

(in thousands)
Research and development
General and administrative
Total stock-based compensation expense

Stock Option Activity

Year Ended
December 31, 

2022
3,619
5,543
9,162

$

$

$

2021
2,759
8,418
$ 11,177

During the year ended December 31, 2022, and 2021 the Company granted options to purchase 767,913 and

406,752 shares of common stock, respectively. For the years ended December 31, 2022, and 2021, amortization of stock
compensation of options amounted to $7.8 million and $9.3 million, respectively. As of December 31, 2022, the total
unrecognized stock-based compensation balance for unvested options was $8.1 million, which is expected to be recognized
over 2.2 years. The weighted-average fair value of options granted during the years ended December 31, 2022, and
December 31, 2021, were $1.79 per share and $8.43 per share, respectively.

The following table summarizes the information about options outstanding at December 31, 2022:

Options

  Weighted-
Average

Outstanding Exercise Price 
$

     Weighted-Average     
Remaining
Contractual
Term (in years)
7.7

  Aggregate
Intrinsic
Value
$ 10,305

(in thousands, except for share data)
Outstanding at December 31, 2021

Options granted
Options exercised
Forfeited
Expired

Outstanding at December 31, 2022

  4,704,888
767,913
(47,602)
(377,378)
(173,774)
  4,874,047

Exercisable at December 31, 2022
Nonvested at December 31, 2022

  3,859,880
  1,014,167

F-22

13.29
1.39
1.04
19.90
26.82
1.97

2.21
1.05

$

$
$

21

—

—
—

6.9

6.6
8.3

$

$
$

    
    
 
 
    
    
 
 
 
 
 
 
 
 
 
Table of Contents

Valuation of Stock Options Granted to Employees that Contain Service Conditions Only

The fair value of each option award granted with service-based vesting is estimated on the date of the grant using

the Black-Scholes option valuation model based on the weighted average assumptions noted in the table below for those
options granted in the years ended December 31, 2022 and 2021.

Expected term (in years)
Volatility
Risk-free interest rate
Dividend yield

Restricted Stock Unit Activity

Year Ended
December 31, 

2022

2021

5.7
75.83 %
2.13 %
— %

5.8
71.92 %
1.08 %
— %

During the year ended December 31, 2022, the Company granted 605,600 restricted stock units (“RSUs”). For the

years ended December 31, 2022 and December 31, 20201 amortization of stock compensation of RSUs amounted to $1.3
million and $1.9 million, respectively. As of December 31, 2022, the unamortized compensation costs associated with non-
vested restricted stock awards was $3.5 million with a weighted-average remaining amortization period of 3.2 years.

The following table summarizes the information about restricted stock units outstanding at December 31, 2022:

(in thousands, except for share data)
Outstanding at December 31, 2021

Awarded
Released
Forfeited

Outstanding at December 31, 2022
Nonvested at December 31, 2022

  Weighted-Average  
Grant Date
Fair Value

Aggregate
Intrinsic Value
4,202

18.05 $
2.33
24.57
18.10

5.96 $
5.73 $

620
582

Shares
  469,485 $
  605,600
(50,242)
  (209,334)
  815,509 $
  815,509 $

Weighted Average Remaining Recognition Period (in
years)

3.2

2019 Employee Stock Purchase Plan

In May 2019, the Company’s Board and its stockholders approved the 2019 Employee Stock Purchase Plan (the

“ESPP”), which became effective as of May 13, 2019. The ESPP is intended to qualify as an “employee stock purchase
plan” within the meaning of Section 423 of the U.S. Internal Revenue Code of 1986, as amended. The number of shares of
common stock initially reserved for issuance under the ESPP was 180,000 shares. The ESPP provides for an annual
increase on the first day of each year beginning in 2020 and ending in 2029, in each case subject to the approval of the
Board, equal to the lesser of (i) 1% of the shares of common stock outstanding on the last day of the calendar month before
the date of the automatic increase and (ii) 360,000 shares; provided that prior to the date of any such increase, the Board
may determine that such increase will be less than the amount set forth in clauses (i) and (ii). As of December 31, 2022, no
shares of common stock had been issued under the ESPP. The first offering period has not yet been decided by the Board.

8. STOCKHOLDERS’ EQUITY

As of December 31, 2022, the authorized capital stock of the Company consists of 200,000,000 shares of common

stock, par value $0.0001 per share and 10,000,000 shares of preferred stock, par value $0.0001 per share. As of

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December 31, 2021, the authorized capital stock of the Company consists of 100,000,000 shares of common stock, par
value $0.0001 per share and 10,000,000 shares of preferred stock, par value $0.0001 per share.

Common Stock

Voting

The holders of the common stock are entitled to one vote for each share of common stock held at all meetings of

the stockholders. There is no cumulative voting.

Goldman Equity Distribution Agreement

In June 2020, the Company entered into the Goldman Equity Distribution Agreement to sell shares of the

Company’s common stock, from time to time, having an aggregate offering price of up to $100.0 million.  The issuance 
and sale of shares of common stock by the Company pursuant to the Goldman Equity Distribution Agreement is deemed an 
“at-the-market” offering under the Securities Act of 1933, as amended, or the Securities Act.  Goldman is entitled to 
compensation for its services equal to up to 3.0% of the gross offering proceeds of all shares of the Company’s common 
stock sold through it as a sales agent pursuant to the Goldman Equity Distribution Agreement.  The Goldman Equity 
Distribution Agreement was terminated as of January 24, 2022.

Cowen Equity Distribution Agreement

On January 26, 2022, the Company entered into the Cowen Equity Distribution Agreement to sell shares of the
Company’s common stock, from time to time, having an aggregate offering price of up to $100.0 million. Pursuant to the
Cowen Equity Distribution Agreement shares of our common stock may be offered and sold through the sales agent in
sales deemed “at-the-market” offerings under the Securities Act of 1933, as amended, or the Securities Act. Under the
Cowen Equity Distribution Agreement, the sales agent will be entitled to compensation of up to 3% of the gross offering
proceeds of all shares of our common stock sold through it pursuant to the Cowen Equity Distribution Agreement. In
connection with the sale of shares of our common stock on our behalf, the sales agent may be deemed to be “underwriters”
within the meaning of the Securities Act, and the compensation paid to the sales agent may be deemed to be underwriting
commissions or discounts. As of December 31, 2022, the Company has not sold any shares of common stock pursuant to
the Cowen Equity Distribution Agreement.

June 2022 Offering

On June 27, 2022, the Company completed the June Offering, an underwritten public offering of 20,000,000
shares of common stock, par value $0.0001 per share, 10,000,000 Pre-Funded Warrants, and accompanying Common
Warrants to purchase up to 30,000,000 shares of common stock. The shares and accompanying Common Warrants were
offered at a price to the public of $1.00 per share and warrant, and the Pre-Funded Warrants and accompanying Common
Warrants were offered at a price to the public of $0.9999, resulting in aggregate net proceeds of approximately $27.8
million, after deducting underwriting discounts and commissions and offering expenses. The Pre-Funded Warrants and the
Common Warrants are immediately exercisable and will expire five years from the date of issuance. Holders may not
exercise any Pre-Funded Warrants or Common Warrants that would cause the aggregate number of shares of common
stock beneficially owned by the holder to exceed 9.99% of the Company’s outstanding common stock immediately after
exercise. Holders of the Pre-Funded Warrants and/or Common Warrants (together with affiliates) who immediately prior to
June 27, 2022 beneficially owned more than 9.99% of the Company’s outstanding common stock may not exercise any
portion of their Pre-Funded Warrants or Common Warrants if the holder (together with affiliates) would beneficially own
more than 19.99% of the Company’s outstanding common stock after exercise. The Pre-Funded Warrants and Common
Warrants are subject to adjustment in the event of certain stock dividends and distributions, stock splits, stock
combinations, reclassifications or similar events affecting the common stock and also upon any distributions for no
consideration of assets to the Company’s stockholders. In the event of certain corporate transactions, the holders of the Pre-
Funded Warrants and/or Common Warrants will be entitled to receive, upon exercise, the kind and amount of securities,
cash or other property that the holders would have received had they exercised the Pre-Funded Warrants and/or Common
Warrants immediately prior to such transaction. The Pre-Funded Warrants and Common Warrants do

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not entitle the holders thereof to any voting rights or any of the other rights or privileges to which the Company’s
stockholders are entitled. The Company intends to use the net proceeds from the June Offering for general corporate
purposes, which may include research and development costs, including the conduct of clinical trials and process
development and manufacturing of the Company’s product candidates, expansion of the Company’s research and
development capabilities, working capital and capital expenditures.

9. WARRANTS

Warrants Issued with Series A Preferred Stock

On January 26, 2017, in connection with the sale and issuance of the Series A Preferred Stock, the Company

issued equity-classified warrants to purchase 309,389 shares of common stock (the “2017 Warrants”), valued at
$0.2 million, and included in the issuance costs of the Series A Preferred Stock. The warrants vested immediately and have
an exercise price of $2.49 per share and expire on March 13, 2027.

The fair value of warrants issued is estimated using the Black-Scholes option pricing model with the following

assumptions for the 2017 Warrants.

Contractual term (in years)
Volatility
Risk-free interest rate
Dividend yield

10.0  
74.48 %
3.20 %
0.00 %

On December 5, 2019, an optionholder exercised 20,000 options in a cashless exercise at net, and the Company

issued 17,026 shares of common stock.

On February 21, 2020, two warrantholders exercised 185,634 options in a cashless exercise at net, and the

Company issued 176,092 shares of common stock. On February 24, 2020, a warrantholder exercised 72,818 options in a
cashless exercise at net, and the Company issued 69,094 shares of common stock.

On February 5, 2021, a warrantholder exercised 27,855 warrants on a cash basis and received 27,855 shares of

common stock. The Company received $69,000 in cash proceeds for the exercise of these warrants.

Warrants Issued with the 2018 Notes

On January 18, 2018, the Company entered into a placement agent agreement through which it became obligated
to issue common stock warrants in connection with the issuance of the Company’s convertible promissory notes issued on
February 5, 2018 (the “2018 Notes”). The obligation to issue the 2018 Notes Warrants was recorded as a liability at its fair
value (see Note 3), which was initially $0.1 million, and was included in the issuance costs of the 2018 Notes. On
November 5, 2018, in connection with the extinguishment of the 2018 Notes into shares of Series B Preferred Stock, the
Company issued the 2018 Notes Warrants, which were equity-classified warrants upon issuance, to purchase 76,847 shares
of common stock, valued at $0.3 million. The 2018 Notes Warrants vested immediately upon issuance and have an exercise
price of $6.59 per share and expire on November 4, 2028.

On February 24, 2020, a warrantholder exercised 386 options in a cashless exercise at net, and the Company

issued 333 shares of common stock. On June 24, 2020, a warrantholder exercised 20,331 options in a cashless exercise at
net, and the Company issued 17,369 shares of common stock.

Warrants Issued with Series B Preferred Stock

In November and December 2018, in connection with the sale and issuance of the Series B Preferred Stock, the
Company was obligated to issue equity-classified warrants to purchase 72,261 shares of common stock (collectively the
“2018 Warrants”), valued in the aggregate at $0.2 million, which was included in the issuance costs for the Series B

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Preferred Stock. The warrants vest immediately upon issuance, have an exercise price of $8.24 per share and expire 10
years from the date of issuance.

The fair value of the 2018 Warrants is estimated using the Black-Scholes option pricing model with the following

assumptions:

Contractual term (in years)
Volatility
Risk-free interest rate
Dividend yield

10.0  
73.22 %
2.70 %
0.00 %

In February 2019, in connection with the sale and issuance of the Series B Preferred Stock, the Company was

obligated to issue warrants to purchase 23,867 shares of common stock (collectively the “2019 Warrants”), valued in the
aggregate at $0.1 million, which was included in the issuance costs for the Series B Preferred Stock. The warrants vest
immediately upon issuance, have an exercise price of $8.24 per share and expire 10 years from the date of issuance.

The fair value of the 2019 Warrants was estimated using the Black-Scholes option pricing model with the

following assumptions:

Contractual term (in years)
Volatility
Risk-free interest rate
Dividend yield

10.0  
73.22 %
2.70 %
0.00 %

The inputs utilized by management to value the warrants are highly subjective. The assumptions used in

calculating the fair value of the warrants represent the Company’s best estimates, but these estimates involve inherent
uncertainties and the application of management judgment. As a result, if factors change and the Company uses different
assumptions, the fair value of the warrants may be materially different in the future.

Warrants Issued with June 2022 Offering

On June 27, 2022, in connection with the sale and issuance common stock as part of the June Offering, the
Company issued 10,000,000 Pre-Funded Warrants at an exercise price of $0.0001 per share, and 30,000,000 accompanying
Common Warrants at an exercise price of $1.00 per share. Each share of common stock and accompanying Common
Warrant was sold at a public offering price of $1.00, less underwriting discounts and commissions, and each Pre-Funded
Warrant and accompanying Common Warrant was sold at a public offering price of $0.9999, less underwriting discounts
and commissions, as described in the prospectus supplement, dated June 22, 2022, filed with the Securities and Exchange
Commission on June 24, 2022.

The Pre-Funded Warrants and the Common Warrants are immediately exercisable and will expire five years from

the date of issuance. Holders may not exercise any Pre-Funded Warrants or Common Warrants that would cause the
aggregate number of shares of common stock beneficially owned by the holder to exceed 9.99% of the Company’s
outstanding common stock immediately after exercise. Holders of the Pre-Funded Warrants and/or Common Warrants
(together with affiliates) who immediately prior to June 27, 2022 beneficially owned more than 9.99% of the Company’s
outstanding common stock may not exercise any portion of their Pre-Funded Warrants or Common Warrants if the holder
(together with affiliates) would beneficially own more than 19.99% of the Company’s outstanding common stock after
exercise. The Pre-Funded Warrants and Common Warrants are subject to adjustment in the event of certain stock dividends
and distributions, stock splits, stock combinations, reclassifications or similar events affecting the common stock and also
upon any distributions for no consideration of assets to the Company’s stockholders. In the event of certain corporate
transactions, the holders of the Pre-Funded Warrants and/or Common Warrants will be entitled to receive, upon exercise,
the kind and amount of securities, cash or other property that the holders would have received had they exercised the Pre-
Funded Warrants and/or Common Warrants immediately prior to such transaction. The Pre-

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Funded Warrants and Common Warrants do not entitle the holders thereof to any voting rights or any of the other rights or
privileges to which the Company’s stockholders are entitled.

On June 28, 2022, a warrantholder exercised 1,750,000 Pre-Funded Warrants on a cash basis and received

1,750,000 shares of common stock. The Company received $175 in cash proceeds for the exercise of these Pre-Funded
Warrants.

As of December 31, 2022, the Company had 8,250,000 Pre-Funded Warrants outstanding with a weighted average
exercise price of $0.0001 per share and an average contractual life of 5 years. As of December 31, 2022, the Company had
30,000,000 Common Warrants outstanding with a weighted average exercise price of $1.00 per share and an average
contractual life of 5 years.

The Common Warrants were accounted for as liabilities under ASC 815-40, as these warrants provide for a 

settlement provision that does not meet the requirements of the indexation guidance under ASC 815-40. These warrant 
liabilities are measured at fair value at inception and on a recurring basis, with changes in fair value presented within the 
statement of operations. The Pre-Funded Warrants were initially recorded at fair value as a liability as the Company could 
be required to settle the Pre-Funded Warrants in cash in the event of an acquisition of the Company under certain 
circumstances. In December 2022, the Company amended the Pre-Funded Warrants to remove the potential requirement 
that they could be settled in cash under certain circumstances.  At December 31, 2022, the Pre-funded Warrants are 
recorded as equity, using their fair value as of the amendment date.

The fair value of the Common and Pre-Funded Warrants were estimated using the Black-Scholes option pricing

model with the following assumptions:

Expected term (in years)
Volatility
Risk-free interest rate
Dividend yield

3.7  
91.53 %
4.11 %
0.00 %

A summary of the Company’s outstanding common stock warrants as of December 31, 2022 is as follows:

Outstanding as of December 31, 2021
Warrants granted and issued
Warrants exercised
Warrants exchanged
Outstanding as of December 31, 2022

10. LEASES

Warrants

125,618
  40,000,000
  (1,750,000)
—
38,375,618

The following table summarizes our lease assets and liabilities as of December 31, 2022 and 2021:

ROU Assets and Liabilities
ROU - Asset
Lease liabilities (current)
Lease liabilities (non-current) Operating lease liabilities, non-current

Right-of-use assets
Operating lease liabilities, current

Balance Sheet Location

Operating
(in thousands)

December 31, December 31, 

2022

2021

$

857 $
477  
414  

1,298
442
891

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The following table summarizes our lease related costs for the twelve months ended December 31, 2022 and

2021:

Lease Cost
Operating Lease Cost

Statement of Operations Location
General and administrative

Total Lease Cost

Operating
(in thousands)

2022

2021

489 $
489 $

505
505

$
$

Average lease terms and discount rates for the Company’s operating leases were as follows:

Other Information
Weighted-average remaining lease term

Operating leases

Weighted-average discount rate

Operating leases

Year Ended
December 31,  December 31, 

2022

2021

1.8 years

2.8 years

5.69%

5.69%

The following table summarizes the maturities of lease liabilities as of December 31, 2022:

Year
2023
2024
Thereafter
Total lease payments
Less: interest
Total lease liabilities

11. INCOME TAXES

     Operating
(in thousands)
515
$
425
—
940
49
891

$

The Company’s current tax provision for the years ended December 31, 2022 and 2021 is $0 and $0, respectively.

The Company’s deferred tax provision for the years ended December 31, 2022 and 2021 is $0 and $0, respectively.

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A reconciliation of the Company's deferred taxes is as follows (in thousands):

Year ended
December 31, 

2022

2021

Deferred Tax Assets

Operating Lease Liability
Stock-based compensation
License fee
Net operating loss carryforwards
Research and development tax credits
Capitalized R&D expense
Other

Total Deferred Tax Assets
Valuation Allowance
Net Deferred Tax Assets
Deferred Tax Liabilities
Right of Use Asset

Net Deferred Tax Liabilities
Net deferred tax asset (liability)

$

$

420
282
6,606
8,131
594
554
79,429
88,090
14,940
21,397
—
14,910
1,352
1,085
$ 103,341
$ 134,449
$ (134,177) $ (102,932)
409
$

272

$

(272)
(272) $
— $

(409)
(409)
—

$
$

Deferred tax assets result primarily from unutilized net operating losses, research tax credits,  stock-based 
compensation, operating lease liability, and timing differences as a result of the Company reporting its income tax returns. 
As of December 31, 2022, the Company had approximately $280.6 million of federal operating losses (“NOLs”) carried
forward. Of this amount, approximately $3.3 million will begin to expire in 2037 and approximately $277.3 million are
carried forward indefinitely. The Company had approximately $572.8 million in state and city net operating loss
carryforwards available to offset future taxable income.

As of December 31, 2022, the Company had federal research tax credits (R&D) of approximately $4.9 million
which may be used to offset future tax liabilities. Additionally, the Company had a federal orphan drug credit (“ODC”)
related to qualifying research of $16.5 million. These tax credit carryforwards will begin to expire at various times
beginning in 2037 for federal purposes.

The NOL, R&D and ODC credits carry forwards are subject to review and possible adjustment by the U.S. and

state tax authorities. NOL carry forwards and credit carry forwards may become subject to an annual limitation in the event
of certain cumulative changes in the ownership interest of significant shareholders, as defined under Sections 382 and 383
Internal Revenue Code. This could limit the amount of NOLs and credits that the Company can utilize annually to offset
future taxable income or tax liabilities. As of December 31, 2022, the Company has not performed such an analysis.
Subsequent ownership changes and proposed future changes to tax rules in respect of the utilization of losses carried
forward may further affect the limitation in future years.

In assessing the realizability of the Company’s deferred tax assets, management considers whether or not it is
more likely than not that some portion or all of the deferred tax assets will not be realized. The ultimate realization of
deferred tax assets is dependent upon the generation of future taxable income. The Company’s assessment is based on the
weight of available evidence, including cumulative losses since inception and expected future losses and, as such, the
Company does not believe it is more likely than not that the deferred tax assets will be realized. Accordingly, a full
valuation allowance has been established and no deferred tax assets and related tax benefit have been recognized in the
accompanying financial statements. At December 31, 2022 and 2021, the Company recorded valuation allowances of
$134.2 million and $102.9 million, respectively. The increase in valuation allowance is primarily driven by additional net
operating loss.

The Company files its income tax returns in the United States, New York State, New York City, California,

Massachusetts, and New Jersey. All years remain subject to examination for federal and state purpose.

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The U.S. federal statutory corporate tax rate reconciles to the Company’s effective tax rate for the years ended

December 31, 2022 and 2021:

Federal statutory rate
State and local taxes net of federal tax benefit
Credits
Permanent Differences
Change in valuation allowance
Stock Compensation
Other
Total

Year Ended
December 31, 

2022
21.0 %  
10.2  
7.8  
(0.1) 
(37.9) 
(1.1)
0.1  
0.0%  

2021
21.0 %
10.7
5.6
0.5
(37.7)
—
(0.1)
0.0 %

12. BENEFIT PLANS

The Company established a defined contribution savings plan under Section 401(k) of the Internal Revenue Code

in 2018. This plan covers substantially all employees who meet minimum age and service requirements and allows
participants to defer a portion of their annual compensation on a pre-tax basis. Matching contributions to the plan may be
made at the discretion of the Company’s Board. The Company made approximately $0.4 million and $0.2 million in
matching contributions to the plan during the year ended December 31, 2022 and 2021, respectively.

13. NET LOSS PER COMMON SHARE

Basic net loss per common share is computed by dividing the net loss available to common stockholders by the

weighted-average number of shares of common stock outstanding during the period.

Diluted net loss per common share is computed by giving the effect of all potential shares of common stock,

including stock options, preferred shares, warrants and instruments convertible into common stock, to the extent dilutive.
Basic and diluted net loss per common share was the same for the years ended December 2022 and 2021, as the inclusion
of all potential common shares outstanding would have been anti-dilutive.

The following table sets forth the computation of basic and diluted net loss per common share (in thousands,

except share and per share data):

(in thousands, except for share data)
Numerator:
Net loss
Denominator:

Years Ended
December 31, 

2022

2021

$

(82,508) $

(105,584)

Weighted-average common stock outstanding

  37,825,431

  25,598,181

Net loss per share attributable to common stockholders -  basic 
and diluted

$

(2.18) $

(4.12)

The Company’s potentially dilutive securities, which include restricted stock units, stock options and common
warrants, have been excluded from the computation of diluted net loss per share as the effect would be to reduce the net
loss per share. Therefore, the weighted-average number of common shares outstanding used to calculate both basic and
diluted net loss per share attributable to common stockholders is the same. The Company excluded the following potential
common shares, presented based on amounts outstanding at December 31, 2022 and 2021, from the

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computation of diluted net loss per share attributable to common stockholders because including them would have had an
anti-dilutive effect:

Options to purchase common stock
Restricted stock units
Warrants to purchase common stock

14. RELATED PARTIES

As of
December 31, 

2022
4,874,047
815,509
  30,125,618

2021
4,704,888
469,485
125,618

In December 2018, the Company entered into an agreement (the “LaunchLabs Agreement”) with ARE-

LaunchLabs NYC LLC (“Alexandria LaunchLabs”), a subsidiary of Alexandria Real Estate Equities, Inc. for use of
specified premises within the Alexandria LaunchLabs space on a month-to-month basis. A member of the Company’s
board of directors is the founder and executive chairman of Alexandria Real Estate Equities, Inc. During the years ended
December 31, 2022 and 2021, the Company made payments to Alexandria LaunchLabs of approximately $0.1 million and
$0.1 million, respectively under the LaunchLabs Agreement, which was recognized in research and development expenses.
As of December 31, 2022, there were no amounts due to Alexandria LaunchLabs under the LaunchLabs Agreement.

15. SUBSEQUENT EVENTS

On January 3, 2023, the “Company entered into an Exclusive License and Supply Agreement (the “Agreement”)
with Mercury Pharma Group Limited (trading as Advanz Pharma Holdings), a company organized and existing under the
laws of England and Wales (“ADVANZ PHARMA”), a UK headquartered global pharmaceutical company with a strategic
focus on specialty, hospital, and rare disease medicines in Europe. Pursuant to the Agreement, the Company granted
ADVANZ PHARMA the exclusive right and license to commercialize drug products containing AT-007 (also known as
govorestat), the Company’s proprietary Aldose Reductase Inhibitor (ARI) (the “Licensed Product”), for use in treatment of
sorbitol dehydrogenase deficiency (“SORD”) and Galactosemia in humans (each, a “Licensed Indication”) in the European
Economic Area, Switzerland and the United Kingdom (the “Territory”). The Company also grants ADVANZ PHARMA a
right of negotiation and “most-favored nation” rights with respect to acquiring the European commercialization rights for
any additional indications for which the Licensed Product may be developed in the future (or any other products the
Company may develop solely to the extent used for the Licensed Indications).

ADVANZ PHARMA is required to use commercially reasonable efforts to launch and commercialize the

Licensed Products in the major markets in the Territory in each Licensed Indication following, and subject to, receipt of
marketing authorization therein. Under the Agreement, ADVANZ PHARMA agrees to pay the Company (i) an upfront
payment of EUR 10 million (approx. USD $10.7 million), and certain development milestone payments upon clinical trial
completions and receipt of marketing authorization in the Territory, as well as certain commercial milestone payments,
totaling EUR 134 million (approx. USD $142.2 million) in the aggregate, and (ii) royalties of 20% of net sales of the
Licensed Product. Such royalty rate will be payable on a country-by-country basis until the later of (i) the expiration of the
licensed patents covering the composition of matter of AT-007, or (ii) 10 years after the European Medicines Agency’s
grant of marketing authorization for the Licensed Product. The royalties are subject to certain deductions, including certain
secondary finishing costs, certain step-in establishment costs and a portion of fees for any potential third party patent
licenses if applicable in the future. Following the initial term of the license, as described above, the royalty rate shall be
reduced to 10% and shall continue in perpetuity unless the Agreement is terminated in various circumstances in accordance
with its terms.

Certain of the patents licensed to ADVANZ PHARMA under the Agreement are sub-licensed from the University

of Miami and Columbia University, and thus remain subject to certain obligations of the Company (including royalty
obligations) to such institutions.

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Under the Agreement, the Company remains responsible for development of the Licensed Product, and must

conduct such development through grant of marketing authorizations in the Licensed Indications in the Territory and as
otherwise required under such marketing authorization, in accordance with any timeframe required by regulatory
authorities. The Company retains sole responsibility for the conduct of all clinical trials (subject in some circumstances to
cost-sharing with ADVANZ PHARMA), unless the Company provides ADVANZ PHARMA prior consent to conduct
certain studies following marketing authorization, or ADVANZ PHARMA exercises certain step-in rights (as described
below). The Company also agrees to manufacture and supply the Licensed Product in bulk form to ADVANZ PHARMA.
ADVANZ PHARMA is responsible for secondary packaging and release for the Territory.

The Agreement includes indemnification obligations on the part of both parties for third-party claims arising out

of, among other things, a breach of the Agreement; an election by the other party not to initiate a recall; gross negligence or
willful misconduct; and violation of applicable laws. In addition, both parties have agreed to indemnification obligations
for third party liability product liability claims and certain exclusions from liability disclaimers, such as for breaches of
confidentiality, death or personal injury caused by negligence or willful default.

In certain circumstances, including in the event of specified supply shortages, bankruptcy and certain other

financial events, a force majeure event lasting more than three months, or termination as a result of the Company’s gross
negligence or willful misconduct, ADVANZ PHARMA may exercise certain step-in rights. Such step-in rights include the
ability for ADVANZ PHARMA to perform its own supply arrangements, and in some cases, specified development rights
in the Licensed Indications in the Territory and assignment of certain contract rights. In all such circumstances, ADVANZ
PHARMA must continue to pay royalties and milestone payments. ADVANZ PHARMA may recoup certain of its
manufacturing and development establishment costs, and deduct such costs from royalties.

The Company may terminate the Agreement upon certain specified events, including ADVANZ PHARMA’s

failure to launch or achieve certain sales threshold for the Licensed Product in major markets within a certain timeframe, or
if ADVANZ PHARMA challenges a licensed patent, and either party may terminate the Agreement upon the other party’s
material breach or insolvency, certain material safety issues or a force majeure event of the other party lasting longer than
six months. ADVANZ PHARMA may also terminate the agreement if the Licensed Product does not receive marketing
authorization for use in a Licensed Indication in any country in the Territory by a specified date, or in the event of the
Company’s gross negligence or willful misconduct (subject to a cure period).

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ITEM 9.      CHANGES IN AND DISAGREEMENTS WITH ACCOUNTANTS ON ACCOUNTING AND

FINANCIAL DISCLOSURE.

None.

ITEM 9A.      CONTROLS AND PROCEDURES.

Evaluation of Controls and Procedures

As of December 31, 2022, our management, with the participation of our Chief Executive Officer and our Interim

Principal Financial Officer, evaluated the effectiveness of our disclosure controls and procedures as defined in Rules 13a-
15(e) and 15d-15(e) of the Exchange Act. Disclosure controls and procedures include, without limitation, controls and
procedures designed to ensure that information required to be disclosed by a company in the reports that it files or submits
under the Exchange Act is accumulated and communicated to management, including our principal executive and principal
financial officers, as appropriate to allow timely decisions regarding required disclosure.

Management recognizes that any controls and procedures, no matter how well designed and operated, can provide
only reasonable assurance of achieving their objectives, and management necessarily applies its judgment in evaluating the
cost-benefit relationship of possible controls and procedures. Based on this evaluation, our Chief Executive Officer and
Interim Principal Financial Officer concluded that, as of December 31, 2022, the design and operation of our disclosure
controls and procedures were effective at the reasonable assurance level.

Management’s Annual Report on Internal Control over Financial Reporting

Management of the Company is responsible for establishing and maintaining adequate internal control over

financial reporting as defined in Rules 13a-15(f) and 15d-15(f) under the Exchange Act. Our internal control over financial
reporting is a process designed to provide reasonable assurance regarding the reliability of financial reporting and the
preparation of financial statements for external purposes in accordance with generally accepted accounting principles.
Because of its inherent limitations, internal control over financial reporting may not prevent or detect misstatements. Also,
projections of any evaluation of effectiveness to future periods are subject to the risk that controls may become inadequate
because of changes in conditions, or that the degree of compliance with the policies or procedures may deteriorate.

Management conducted an evaluation of the effectiveness of our internal control over financial reporting as of

December 31, 2022 based on the framework in Internal Control-Integrated Framework (2013) issued by the Committee of
Sponsoring Organizations of the Treadway Commission (COSO). Based on that evaluation, management has concluded
that the Company’s internal control over financial reporting was effective as of December 31, 2022.

Changes in Internal Control over Financial Reporting

There was no change in our internal control over financial reporting identified in connection with the evaluation

required by Rule 13a-15(d) and 15d-15(d) of the Exchange Act that occurred during the fourth quarter of 2022 that has
materially affected, or is reasonably likely to materially affect, our internal control over financial reporting.

ITEM 9B.      OTHER INFORMATION.

None.

ITEM 9C.       DISCLOSURE REGARDING FOREIGN JURISDICTIONS THAT PREVENT INSPECTIONS.

Not Applicable.

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PART III

ITEM 10.      DIRECTORS, EXECUTIVE OFFICERS AND CORPORATE GOVERNANCE.

The information required by Item 10 is incorporated by reference to the information that will be contained in our

2023 Proxy Statement under the captions “Proposal 1 - Election of Directors,” “Principal Stockholders,” “Proposal 2 –
Ratification of Independent Registered Public Accounting Firm” and “Audit Committee Report.”

ITEM 11.      EXECUTIVE AND DIRECTOR COMPENSATION.

The information required by Item 11 is incorporated by reference to the information that will be contained in our

2023 Proxy Statement under the captions “Executive and Director Compensation,” “Compensation Discussion and
Analysis,” “Compensation Committee Report,” “Compensation Committee Interlocks and Insider Participation,”
“Compensation of Named Executives,” “Summary Compensation Table,” “Equity Incentive Plans,” “Non-Employee
Director Compensation,” “Stock Option Grants,” “Outstanding Equity Awards at Fiscal Year-End,” “Health and Welfare
Retirement Benefits,” and “Potential Payments and Benefits Upon Termination or Change-in-Control.”

ITEM 12.      SECURITY OWNERSHIP OF CERTAIN BENEFICIAL OWNERS AND MANAGEMENT AND

RELATED STOCKHOLDER MATTERS.

The information required by Item 12 is incorporated by reference to the information that will be contained in our

2023 Proxy Statement under the caption “Principal Stockholders.”

ITEM 13.   CERTAIN RELATIONSHIPS AND RELATED TRANSACTIONS, AND DIRECTOR

INDEPENDENCE.

The information required by Item 13 is incorporated by reference to the information that will be contained in our

2023 Proxy Statement under the caption “Certain Relationships and Transactions.”

ITEM 14.      PRINCIPAL ACCOUNTANT FEES AND SERVICES.

The information required by Item 14 is incorporated by reference to the information that will be contained in our

2023 Proxy Statement under the caption “Independent Registered Public Accounting Firm”.

95

Table of Contents

ITEM 15.      EXHIBITS, FINANCIAL STATEMENT SCHEDULES.

(a) The following documents are filed as part of this Annual Report   

PART IV

1. Financial Statements:

The following financial statements and schedules of the Registrant are contained in Part II, Item 8, “Financial

Statements and Supplementary Data” of this Annual Report:

Item
Report of Independent Registered Public Accounting Firm PCAOB Firm ID: 00042
Balance Sheets as of December 31, 2022 and 2021
Statements of Operations for the years ended December 31, 2022 and 2021
Statements of Comprehensive Income (Loss) for the years ended December 31, 2022 and 2021
Statement of Changes in Shareholders’ Equity for the years ended December 31, 2021 and 2022
Statements of Cash Flows for the years ended December 31, 2022 and 2021
Notes to Financial Statements

Page
F-1
F-2
F-3
F-4
F-5
F-6
F-7

2. Financial Statement Schedules:

There are no Financial Statement Schedules included with this filing for the reason that they are not applicable or

are not required or the information is included in the financial statements or notes thereto.

(b) Exhibits required by Item 601 of Regulation S-K

The information required by this Item is set forth on the exhibit index that follows the signature page of this

Annual Report.

96

Table of Contents

Exhibit Number
3.1

3.2

3.3+

4.1+

4.2+

4.3+

4.4+

4.5+

4.6+

4.7+

4.8+

EXHIBIT INDEX

Description
Amended and Restated Certificate of
Incorporation of the Registrant, as
amended.

Certificate of Amendment to
Amended and Restated Certificate of
Incorporation of the Registrant.

Amended and Restated Bylaws of the
Registrant.

Registration Rights Agreement, dated
November 7, 2019, by and among the
Registrant and the Purchasers.

Form of Common Stock Certificate of
the Registrant.

Amended and Restated Investors’
Rights Agreement, by and among the
Registrant and certain of its
stockholders, dated November 5,
2018.

Form of Warrant, issued to affiliates of
Brookline Capital Markets, a division
of CIM Securities, LLC on March 13,
2017.

Form of Warrant, issued to affiliates of
Brookline Capital Markets, a division
of CIM Securities, LLC on November
5, 2018.

Form of Warrant, issued to affiliates of
Brookline Capital Markets, a division
of CIM Securities, LLC on April 9,
2019.

Form of Pre-Funded Warrant to
Purchase Common Stock

Form of Common Warrant to Purchase
Common Stock

97

Form   

File No.

Exhibit

Filing Date

8-K

001-
38898

3.1

October
28, 2022

8-K

10-
Q

S-
1/A

S-
1/A

S-
1/A

S-
1/A

8-K

8-K

001-
38898

10.2

November
12, 2019

001-
38898

333-
230838

333-
230838

333-
230838

333-
230838

001-
38898

001-
38898

4.1

4.2

4.3

4.4

4.5

4.1

4.2

August
12, 2019

April 29,
2019

April 29,
2019

April 29,
2019

April 29,
2019

June 27,
2022

June 27,
2022

    
  
  
  
Table of Contents

4.9+

10.1*+

10.2*+

10.3*+

10.4*+

10.5*+

10.6*+

10.7*+

10.8†+

10.9†

10.10*+

10.11*

Description of securities registered
under Section 12 of the Exchange Act.

Forms of Indemnity Agreement by and
between the Registrant and its directors
and executive officers.

2019 Equity Incentive Plan.

Forms of Option Grant Notice and
Option Agreement under 2019 Equity
Incentive Plan.

Form of Restricted Stock Unit Grant
Notice and Unit Award Agreement
under 2019 Equity Incentive Plan.

2016 Equity Incentive Plan, as
amended.

Forms of Stock Option Agreement
under the 2016 Equity Incentive Plan,
as amended.

2019 Employee Stock Purchase Plan

Exclusive License Agreement by and
between the Registrant and The
Trustees of Columbia University in the
City of New York, dated October 26,
2016.

Exclusive License Agreement by and
between the Registrant and Mercury
Pharma Group Limited, dated January
3, 2023.

Employment Agreement, by and
between the Registrant and Riccardo
Perfetti, dated August 28, 2019.

Employment Agreement, by and
between the Registrant and Shoshana
Shendelman, dated March 9, 2020.

98

10-
K

S-
1/A

S-
1/A

S-
1/A

S-
1/A

S-
1/A

S-
1/A

S-
1/A

S-1

001-
38898

333-
230838

333-
230838

333-
230838

333-
230838

333-
230838

333-
230838

333-
230838

333-
230838

4.7

10.1

10.2

10.3

10.4

10.5

10.6

10.7

10.11

March 13,
2020

April 29,
2019

April 29,
2019

April 29,
2019

April 29,
2019

April 29,
2019

April 29,
2019

April 29,
2019

April 12,
2019

10-
Q

10-
K

001-
38898

001-
38898

10.1

November
13, 2019

10.13

March 13,
2020

10-
K

10-
K

001-
38898

10.14

March 13,
2020

001-
38898

10.15

March 10,
2022

Table of Contents

10.12*

10.13*

23.1

31.1

31.2

32.1

32.2

Amendment to Employment
Agreement, by and between the
Registrant and Riccardo Perfetti, dated
March 9, 2020.

Offer Letter, by and between Steven
Ortega and the Registrant, dated
February 1, 2021.

Consent of Ernst & Young LLP, an
Independent Registered Public
Accounting Firm.

Rule 13a-14(a)/15d-14(a) Certification
under the Exchange Act by Shoshana
Shendelman, President and Chief
Executive Officer (Principal Executive
Officer).

Rule 13a-14(a)/15d-14(a) Certification
under the Exchange Act by Steven
Ortega, Chief Accounting Officer
(Interim Principal Financial Officer).

Certification of Chief Executive
Officer pursuant to 18 U.S.C. Section
1350, as adopted pursuant to Section
906 of the Sarbanes-Oxley Act of 2002
Section 1350 Certifications.

Certification of Interim Principal
Financial Officer pursuant to 18 U.S.C.
Section 1350, as adopted pursuant to
Section 906 of the Sarbanes-Oxley Act
of 2002 Section 1350 Certifications.

101.INS

Inline XBRL Instance Document.

101.SCH

101.CAL

101.DEF

XBRL Taxonomy Extension Schema
Document.

XBRL Taxonomy Extension
Calculation Linkbase Document.

XBRL Taxonomy Extensions
Definition Linkbase Document.

99

Table of Contents

101.LAB

101.PRE

104

XBRL Taxonomy Extension Label
Linkbase Document.

XBRL Taxonomy Extension
Presentation Linkbase Document.

Cover Page Interactive Data File
(formatted as Inline XBRL with
applicable taxonomy extension
information contained in Exhibits 101).

* Indicates a management contract or compensatory plan.
† Portions of this exhibit have been omitted.
+ Previously filed.

ITEM 16.

10-K SUMMARY

None.

100

Table of Contents

Pursuant to the requirements of Section 13 or 15(d) of the Securities Exchange Act of 1934, the Company has

duly caused this report to be signed on its behalf by the undersigned, thereunto duly authorized.

SIGNATURES

Dated: March 23, 2023

Applied Therapeutics, Inc.

/s/ Shoshana Shendelman
Name: Shoshana Shendelman, Ph.D.
Title: President and Chief Executive Officer

Pursuant to the requirements of the Securities Exchange Act of 1934, this report has been signed below by the

following persons on behalf of the Company and in the capacities indicated on the 23rd of March 2023.

Name

    Title

/s/ Shoshana Shendelman
Shoshana Shendelman, Ph.D.

Chair of the Board
President and Chief Executive Officer
(Principal Executive Officer)

/s/ Steven Ortega
Steven Ortega

/s/ Les Funtleyder
Les Funtleyder

/s/ Teena Lerner
Teena Lerner, Ph.D.

/s/ Stacy Kanter
Stacy Kanter

/s/ Joel S. Marcus
Joel S. Marcus

/s/ Jay S. Skyler
Jay S. Skyler, M.D., MACP

Chief Accounting Officer
(Principal Accounting Officer and Interim
Principal Financial Officer)

Director

Director

Director

Director

Director

    Date

March 23, 2023

March 23, 2023

March 23, 2023

March 23, 2023

March 23, 2023

March 23, 2023

March 23, 2023

101

Exhibit 3.1

AMENDED AND RESTATED
CERTIFICATE OF INCORPORATION
OF
APPLIED THERAPEUTICS, INC.

Applied Therapeutics, Inc., a corporation organized and existing under and by virtue of the

General Corporation Law of the State of the Delaware, hereby certifies that:

1:

The original name of this corporation was Applied Therapeutics, Inc. and the date
of filing the original Certificate of Incorporation of this corporation with the Secretary of State of
the State of Delaware (the “Secretary”) was January 20, 2016.

2:

The  Amended  and  Restated  Certificate  of  Incorporation,  attached  hereto  as
Exhibit  A,  is  incorporated  herein  by  reference,  and  restates,  integrates  and  further  amends  the
provisions  of  the  Amended  and  Restated  Certificate  of  Incorporation  as  previously  amended  or
supplemented.

3:

This Amended and Restated Certificate of Incorporation has been duly approved

by the Board of Directors of the Corporation.

4:

This  Amended  and  Restated  Certificate  of  Incorporation  was  approved  by  the
holders of the requisite number of shares of said Corporation in accordance with Section 228 of the
Delaware General Corporation Law.  This Amended and Restated Certificate of Incorporation has
been  duly  adopted  in  accordance  with  the  provisions  of  Sections  242  and  245  of  the  Delaware
General Corporation Law by the stockholders of the Corporation.

IN  WITNESS  WHEREOF,  the  Corporation  has  caused  this  Amended  and  Restated
Certificate of Incorporation to be signed by its duly authorized officer this 22nd day of October,
2022.

APPLIED THERAPEUTICS, INC.

By:  /s/ Shoshana Shendelman

Shoshana Shendelman, Ph.D.
President and Chief Executive Officer

  
 
EXHIBIT A
AMENDED AND RESTATED
CERTIFICATE OF INCORPORATION
OF
APPLIED THERAPEUTICS, INC.

I.

The name of the corporation is APPLIED THERAPEUTICS, INC. (the “Corporation”).

II.

The address of the registered office of the Corporation in the State of Delaware is 251 Little
Falls Drive, in the City of Wilmington, County of New Castle, 19808. The name of the registered
agent  of  the  Corporation  in  the  State  of  Delaware  at  such  address  is  the  Corporation  Service
Company.

The  purpose  of  the  Corporation  is  to  engage  in  any  lawful  act  or  activity  for  which  a

corporation may be organized under the Delaware General Corporation Law (the “DGCL”).

III.

IV.

A.

The  Corporation  is  authorized  to  issue  two  classes  of  stock  to  be  designated,
respectively,  “Common  Stock”  and  “Preferred  Stock.”  The  total  number  of  shares  which  the
Corporation is authorized to issue is two hundred ten million (210,000,000) shares. Two hundred
million (200,000,000) shares shall be Common Stock, each having a par value of one-hundredth of
one cent ($0.0001) and ten million (10,000,000) shares shall be Preferred Stock, each having a par
value of one-hundredth of one cent ($0.0001).

B.

The Preferred Stock may be issued from time to time in one or more series.  The
Board of Directors of the Corporation (the “Board of Directors”) is hereby expressly authorized to
provide for the issue of all or any of the shares of the Preferred Stock in one or more series, and to
fix the number of shares and to determine or alter for each such series, such voting powers, full or
limited,  or  no  voting  powers,  and  such  designation,  preferences,  and  relative,  participating,
optional,  or  other  rights  and  such  qualifications,  limitations,  or  restrictions  thereof,  as  shall  be
stated and expressed in the resolution or resolutions adopted by the Board of Directors providing
for the issuance of such shares and as may be permitted by the DGCL.  The Board of Directors is
also expressly authorized to increase or decrease the number of shares of any series subsequent to
the  issuance  of  shares  of  that  series,  but  not  below  the  number  of  shares  of  such  series  then
outstanding.  In case the number of shares of any series shall be decreased in accordance with the
foregoing sentence, the shares constituting such decrease shall resume the status that they had prior
to the adoption of the resolution originally fixing the number of shares of such series.  The number
of authorized shares of Preferred Stock may be increased or decreased (but not below the number
of  shares  thereof  then  outstanding)  by  the  affirmative  vote  of  the  holders  of  a  majority  of  the
voting  power  of  the  outstanding  shares  of  stock  of  the  Corporation  entitled  to  vote,  without  a
separate vote of the holders of the Preferred Stock, or of any series thereof irrespective of Section
242(b)(2)

6

of the DGCL, unless a vote of any such holders is required pursuant to the terms of any certificate
of designation filed with respect to any series of Preferred Stock.

C.

Each  outstanding  share  of  Common  Stock  shall  entitle  the  holder  thereof  to  one
vote  on  each  matter  properly  submitted  to  the  stockholders  of  the  Corporation  for  their  vote;
provided, however, that, except as otherwise required by law, holders of Common Stock shall not
be entitled to vote on any amendment to this Amended and Restated Certificate of Incorporation
(including  any  certificate  of  designation  filed  with  respect  to  any  series  of  Preferred  Stock)  that
relates  solely  to  the  terms  of  one  or  more  outstanding  series  of  Preferred  Stock  if  the  holders  of
such affected series are entitled, either separately or together as a class with the holders of one or
more  other  such  series,  to  vote  thereon  by  law  or  pursuant  to  this  Amended  and  Restated
Certificate of Incorporation (including any certificate of designation filed with respect to any series
of Preferred Stock).

V.

For the management of the business and for the conduct of the affairs of the Corporation, and in
further definition, limitation and regulation of the powers of the Corporation, of its directors and of
its stockholders or any class thereof, as the case may be, it is further provided that:

A.

MANAGEMENT OF BUSINESS.

The management of the business and the conduct of the affairs of the Corporation shall be
vested  in  its  Board  of  Directors.    The  number  of  directors  which  shall  constitute  the  Board  of
Directors shall be fixed exclusively by resolutions adopted by a majority of the authorized number
of directors constituting the Board of Directors.

B.

BOARD OF DIRECTORS.

Subject  to  the  rights  of  the  holders  of  any  series  of  Preferred  Stock  to  elect  additional
directors  under  specified  circumstances,  following  the  closing  of  the  initial  public  offering
pursuant to an effective registration statement under the Securities Act of 1933, as amended (the
“1933  Act”),  covering  the  offer  and  sale  of  Common  Stock  to  the  public  (the  “Initial  Public
Offering”),  the  directors  shall  be  divided  into  three  classes  designated  as  Class  I,  Class  H  and
Class  III,  respectively.   The  Board  of  Directors  is  authorized  to  assign  members  of  the  Board  of
Directors already in office to such classes at the time the classification becomes effective.  At the
first annual meeting of stockholders following the closing of the Initial Public Offering, the term of
office of the Class I directors shall expire and Class I directors shall be elected for a full term of
three  years.    At  the  second  annual  meeting  of  stockholders  following  the  closing  of  the  Initial
Public Offering, the term of office of the Class II directors shall expire and Class II directors shall
be elected for a full term of three years.  At the third annual meeting of stockholders following the
closing of the Initial Public Offering, the term of office of the Class III directors shall expire and
Class  III  directors  shall  be  elected  for  a  full  term  of  three  years.    At  each  succeeding  annual
meeting  of  stockholders,  directors  shall  be  elected  for  a  full  term  of  three  years  to  succeed  the
directors of the class whose terms expire at such annual meeting.

Notwithstanding the foregoing provisions of this section, each director shall serve until his
or  her  successor  is  duly  elected  and  qualified  or  until  his  or  her  earlier  death,  resignation  or
removal.  

6

No decrease in the number of directors constituting the Board of Directors shall shorten the term of
any incumbent director.

C.

REMOVAL OF DIRECTORS.

Subject  to  the  rights  of  any  series  of  Preferred  Stock  to  elect  additional  directors  under
specified circumstances, following the closing of the Initial Public Offering, neither the Board of
Directors nor any individual director may be removed without cause.

Subject  to  any  limitation  imposed  by  applicable  law,  any  individual  director  or  directors
may  be  removed  with  cause  by  the  affirmative  vote  of  the  holders  of  at  least  sixty-six  and  two-
thirds percent (66 2/3%) of the voting power of all then outstanding shares of capital stock of the
Corporation entitled to vote generally at an election of directors.

D.

VACANCIES.

Subject to any limitations imposed by applicable law and subject to the rights of the holders
of  any  series  of  Preferred  Stock,  any  vacancies  on  the  Board  of  Directors  resulting  from  death,
resignation, disqualification, removal or other causes and any newly created directorships resulting
from any increase in the number of directors, shall, unless the Board of Directors determines by
resolution that any such vacancies or newly created directorships shall be filled by the stockholders
and  except  as  otherwise  provided  by  applicable  law,  be  filled  only  by  the  affirmative  vote  of  a
majority of the directors then in office, even though less than a quorum of the Board of Directors,
and not by the stockholders.  Any director elected in accordance with the preceding sentence shall
hold office for the remainder of the full term of the director for which the vacancy was created or
occurred and until such director’s successor shall have been elected and qualified.

E.

BYLAW AMENDMENTS.

The Board of Directors is expressly empowered to adopt, amend or repeal the Bylaws of
the  Corporation.   Any  adoption,  amendment  or  repeal  of  the  Bylaws  of  the  Corporation  by  the
Board of Directors shall require the approval of a majority of the authorized number of directors.
 The stockholders shall also have power to adopt, amend or repeal the Bylaws of the Corporation;
provided, however, that, in addition to any vote of the holders of any class or series of stock of the
Corporation required by law or by this Amended and Restated Certificate of Incorporation, such
action by stockholders shall require the affirmative vote of the holders of at least sixty-six and two-
thirds  percent  (66  2/3%)  of  the  voting  power  of  all  of  the  then-outstanding  shares  of  the  capital
stock of the Corporation entitled to vote generally in the election of directors, voting together as a
single class.

F.

STOCKHOLDER ACTIONS.

1.

The directors of the Corporation need not be elected by written ballot unless

the Bylaws so provide.

2.

No action shall be taken by the stockholders of the Corporation except at an

annual or special meeting of stockholders called in accordance with the Bylaws, and no action
shall be taken by the stockholders by written consent or electronic transmission.

6

3.

Advance notice of stockholder nominations for the election of directors and

of business to be brought by stockholders before any meeting of the stockholders of the
Corporation shall be given in the manner provided in the Bylaws of the Corporation.

VI.

A.

The liability of the directors for monetary damages shall be eliminated to the fullest

extent under applicable law.

B.

To  the  fullest  extent  permitted  by  applicable  law,  the  Corporation  is  authorized  to
provide indemnification of (and advancement of expenses to) directors, officers and agents of the
Corporation  (and  any  other  persons  to  which  applicable  law  permits  the  Corporation  to  provide
indemnification) through Bylaw provisions, agreements with such agents or other persons, vote of
stockholders  or  disinterested  directors  or  otherwise  in  excess  of  the  indemnification  and
advancement  otherwise  permitted  by  such  applicable  law.    If  applicable  law  is  amended  after
approval by the stockholders of this Article VI to authorize corporate action further eliminating or
limiting the personal liability of directors, then the liability of a director to the Corporation shall be
eliminated or limited to the fullest extent permitted by applicable law as so amended.

C.

Any repeal or modification of this Article VI shall only be prospective and shall not
affect the rights or protections or increase the liability of any director under this Article VI in effect
at  the  time  of  the  alleged  occurrence  of  any  act  or  omission  to  act  giving  rise  to  liability  or
indemnification.

VII.

A.

Unless the Corporation consents in writing to the selection of an alternative forum,
the  Court  of  Chancery  of  the  State  of  Delaware  (or,  if  and  only  if  the  Court  of  Chancery  of  the
State  of  Delaware  lacks  subject  matter  jurisdiction,  any  state  court  located  within  the  State  of
Delaware or, if and only if all such state courts lack subject matter jurisdiction, the federal district
court for the District of Delaware) shall be the sole and exclusive forum for the following types of
actions  or  proceedings  under  Delaware  statutory  or  common  law:    (A)  any  derivative  action  or
proceeding brought on behalf of the Corporation; (B) any action or proceeding (including any class
action)  asserting  a  claim  of  breach  of  a  fiduciary  duty  owed  by  any  current  or  former  director,
officer or other employee of the Corporation, to the Corporation or the Corporation’s stockholders;
(C) any action or proceeding (including any class action) asserting a claim against the Corporation
or any current or former director, officer, employee or agent of the Corporation, arising out of or
pursuant to any provision of the DGCL, this Amended and Restated Certificate of Incorporation or
the  Bylaws  of  the  Corporation  (as  each  may  be  amended  from  time  to  time);  (D)  any  action  or
proceeding  to  interpret,  apply,  enforce  or  determine  the  validity  of  this  Amended  and  Restated
Certificate of Incorporation or the Bylaws of the Corporation (including any right, obligation, or
remedy thereunder); (E) any action or proceeding as to which the DGCL confers jurisdiction to the
Court  of  Chancery  of  the  State  of  Delaware;  (F)  any  action  asserting  a  claim  against  the
Corporation or any director, officer or other employee of the Corporation, governed by the internal
affairs doctrine, in all cases to the fullest extent permitted by law and subject to the court’s having
personal jurisdiction over the indispensable parties named as defendants.  This Section A of Article
VII shall not apply to suits brought to enforce a duty or liability created by the Securities Exchange

6

Act of 1934, as amended, the Securities Act of 1933, as amended, or any other claim for which the
federal courts have exclusive jurisdiction.

B.

Any  person  or  entity  purchasing,  holding,  owning  or  otherwise  acquiring  any
interest in any security of the Corporation shall be deemed to have notice of and consented to the
provisions of this Amended and Restated Certificate of Incorporation.

VIII.

A.

The Corporation reserves the right to amend, alter, change or repeal any provision
contained  in  this  Amended  and  Restated  Certificate  of  Incorporation,  in  the  manner  now  or
hereafter  prescribed  by  statute,  except  as  provided  in  paragraph  B.  of  this  Article  VIII,  and  all
rights conferred upon the stockholders herein are granted subject to this reservation.

B.

Notwithstanding any other provisions of this Amended and Restated Certificate of
Incorporation or any provision of law which might otherwise permit a lesser vote or no vote, but in
addition to any affirmative vote of the holders of any particular class or series of the Corporation
required by law or by this Amended and Restated Certificate of Incorporation or any certificate of
designation filed with respect to a series of Preferred Stock, the affirmative vote of the holders of
at  least  sixty-six  and  two-thirds  percent  (66  2/3%)  of  the  voting  power  of  all  of  the  then
outstanding shares of capital stock of the Corporation entitled to vote generally in the election of
directors, voting together as a single class, shall be required to alter, amend or repeal Articles V, VI
and VII.

* * * *

6

Exhibit 3.3

AMENDED AND RESTATED BYLAWS

OF

APPLIED THERAPEUTICS, INC.
(A DELAWARE CORPORATION)

March 16, 2021

Table of Contents

ARTICLE I OFFICES

Section 1. Registered Office
Section 2. Other Offices

ARTICLE II CORPORATE SEAL

Section 3. Corporate Seal

ARTICLE III STOCKHOLDERS’ MEETINGS

Section 4. Place of Meetings
Section 5. Annual Meetings.
Section 6. Special Meetings.
Section 7. Notice of Meetings
Section 8. Quorum
Section 9. Adjournment and Notice of Adjourned Meetings
Section 10. Voting Rights
Section 11. Joint Owners of Stock
Section 12. List of Stockholders
Section 13. Action Without Meeting
Section 14. Organization.

ARTICLE IV DIRECTORS

Section 15. Number and Term of Office
Section 16. Powers
Section 17. Classes of Directors.
Section 18. Vacancies.
Section 19. Resignation
Section 20. Removal
Section 21. Meetings.
Section 22. Quorum and Voting.
Section 23. Action Without Meeting
Section 24. Fees and Compensation
Section 25. Committees.
Section 26. Duties of Chairperson of the Board of Directors and Lead Independent

Director.

Section 27. Organization

ARTICLE V OFFICERS

Section 28. Officers Designated
Section 29. Tenure and Duties of Officers.
Section 30. Delegation of Authority
Section 31. Resignations
Section 32. Removal

ARTICLE VI EXECUTION OF CORPORATE INSTRUMENTS AND VOTING OF

SECURITIES OWNED BY THE CORPORATION

i

Page

1

1
1

1

1

1

1
1
5
6
7
7
7
8
8
8
8

9

9
9
9
10
10
11
11
12
12
12
12

14
14

14

14
14
16
16
16

17

Table of Contents
(continued)

Section 33. Execution of Corporate Instruments
Section 34. Voting of Securities Owned By the Corporation

ARTICLE VII SHARES OF STOCK

Section 35. Form and Execution of Certificates
Section 36. Lost Certificates
Section 37. Transfers.
Section 38. Fixing Record Dates.
Section 39. Registered Stockholders

ARTICLE VIII OTHER SECURITIES OF THE CORPORATION

Section 40. Execution of Other Securities

ARTICLE IX DIVIDENDS

Section 41. Declaration of Dividends
Section 42. Dividend Reserve

ARTICLE X FISCAL YEAR

Section 43. Fiscal Year

ARTICLE XI INDEMNIFICATION

Page

17
17

17

17
17
18
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Section 44. Indemnification of Directors, Executive Officers, Other Officers, Employees
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and Other Agents.

ARTICLE XII NOTICES

Section 45. Notices.

ARTICLE XIII AMENDMENTS

Section 46. [  ]

ARTICLE XIV LOANS TO OFFICERS

Section 47. Loans to Officers

ii

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AMENDED AND RESTATED BYLAWS

OF

APPLIED THERAPEUTICS, INC.
(A DELAWARE CORPORATION)

March 16, 2021

ARTICLE I

OFFICES

Section 1.

Registered Office.  The registered office of Applied Therapeutics, Inc. (the
“Corporation”)  in  the  State  of  Delaware  shall  be  2711  Centerville  Road,  Suite  400,  City  of
Wilmington, County of New Castle 19808.

Section 2.

Other Offices.  The Corporation shall also have and maintain an office or
principal  place  of  business  at  such  place  as  may  be  fixed  by  the  Board  of  Directors  of  the
Corporation  (the  “Board  of  Directors”),  and  may  also  have  offices  at  such  other  places,  both
within  and  without  the  State  of  Delaware,  as  the  Board  of  Directors  may  from  time  to  time
determine or the business of the Corporation may require.

ARTICLE II

CORPORATE SEAL

Section 3.

Corporate  Seal.    The  Board  of  Directors  may  adopt  a  corporate  seal.    If
adopted,  the  corporate  seal  shall  consist  of  a  die  bearing  the  name  of  the  Corporation  and  the
inscription, “Corporate Seal-Delaware.”  Said seal may be used by causing it or a facsimile thereof
to be impressed or affixed or reproduced or otherwise.

ARTICLE III

STOCKHOLDERS’ MEETINGS

Section 4.

Place of Meetings.  Meetings of the stockholders of the Corporation may be
held at such place, either within or without the State of Delaware, as may be determined from time
to time by the Board of Directors.  The Board of Directors may, in its sole discretion, determine
that the meeting shall not be held at any place, but may instead be held solely by means of remote
communication as provided under the Delaware General Corporation Law (“DGCL”).

Section 5.

Annual Meetings.

(a)

The annual meeting of the stockholders of the Corporation, for the purpose
of election of directors and for such other business as may properly come before it, shall be held on
such  date  and  at  such  time  as  may  be  designated  from  time  to  time  by  the  Board  of  Directors.
 Nominations of persons for election to the Board of Directors of the Corporation and the proposal
of business to be considered by the stockholders may be made at an annual meeting of

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stockholders:  (i) pursuant to the Corporation’s notice of meeting of stockholders (with respect to
business  other  than  nominations);  (ii)  brought  specifically  by  or  at  the  direction  of  the  Board  of
Directors;  or  (iii)  by  any  stockholder  of  the  Corporation  who  was  a  stockholder  of  record  at  the
time of giving the stockholder’s notice provided for in Section 5(b) below, who is entitled to vote
at  the  meeting  and  who  complied  with  the  notice  procedures  set  forth  in  Section  5.    For  the
avoidance  of  doubt,  clause  (iii)  above  shall  be  the  exclusive  means  for  a  stockholder  to  make
nominations and submit other business (other than matters properly included in the Corporation’s
notice  of  meeting  of  stockholders  and  proxy  statement  under  Rule  14a-8  under  the  Securities
Exchange  Act  of  1934,  as  amended,  and  the  rules  and  regulations  thereunder  (the  “1934  Act”))
before an annual meeting of stockholders.

(b)

At  an  annual  meeting  of  the  stockholders,  only  such  business  shall  be
conducted as is a proper matter for stockholder action under Delaware law and as shall have been
properly brought before the meeting.

(i)

For  nominations  for  the  election  to  the  Board  of  Directors  to  be
properly brought before an annual meeting by a stockholder pursuant to clause (iii) of Section 5(a)
of  these  Amended  and  Restated  Bylaws  (these  “Bylaws”),  the  stockholder  must  deliver  written
notice to the Secretary of the Corporation at the principal executive offices of the Corporation on a
timely basis as set forth in Section 5(b)(iii) and must update and supplement such written notice on
a timely basis as set forth in Section 5(c).  Such stockholder’s notice shall set forth:  (A) as to each
nominee  such  stockholder  proposes  to  nominate  at  the  meeting:    (1)  the  name,  age,  business
address  and  residence  address  of  such  nominee;  (2)  the  principal  occupation  or  employment  of
such nominee; (3) the class and number of shares of each class of capital stock of the Corporation
which are owned of record and beneficially by such nominee; (4) the date or dates on which such
shares were acquired and the investment intent of such acquisition; (5) a statement whether such
nominee,  if  elected,  intends  to  tender,  promptly  following  such  person’s  failure  to  receive  the
required  vote  for  election  or  re-election  at  the  next  meeting  at  which  such  person  would  face
election or re-election, an irrevocable resignation effective upon acceptance of such resignation by
the  Board  of  Directors;  and  (6)  such  other  information  concerning  such  nominee  as  would  be
required to be disclosed in a proxy statement soliciting proxies for the election of such nominee as
a director in an election contest (even if an election contest is not involved), or that is otherwise
required  to  be  disclosed  pursuant  to  Section  14  of  the  1934  Act  and  the  rules  and  regulations
promulgated thereunder (including such person’s written consent to being named as a nominee and
to  serving  as  a  director  if  elected);  and  (B)  the  information  required  by  Section  5(b)(iv).    The
Corporation  may  require  any  proposed  nominee  to  furnish  such  other  information  as  it  may
reasonably  require  to  determine  the  eligibility  of  such  proposed  nominee  to  serve  as  an
independent  director  of  the  Corporation  or  that  could  be  material  to  a  reasonable  stockholder’s
understanding of the independence, or lack thereof, of such proposed nominee.

(ii)

Other  than  proposals  sought  to  be  included  in  the  Corporation’s
proxy materials pursuant to Rule 14a-8 under the 1934 Act, for business other than nominations for
the  election  to  the  Board  of  Directors  to  be  properly  brought  before  an  annual  meeting  by  a
stockholder pursuant to clause (iii) of Section 5(a) of these Bylaws, the stockholder must deliver
written  notice  to  the  Secretary  of  the  Corporation  at  the  principal  executive  offices  of  the
Corporation  on  a  timely  basis  as  set  forth  in  Section  5(b)  (iii),  and  must  update  and  supplement
such written notice on a timely basis as set forth in Section 5(c).  Such stockholder’s notice shall

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set  forth:    (A)  as  to  each  matter  such  stockholder  proposes  to  bring  before  the  meeting,  a  brief
description  of  the  business  desired  to  be  brought  before  the  meeting,  the  reasons  for  conducting
such business at the meeting, and any material interest (including any anticipated benefit of such
business to any Proponent (as defined below) other than solely as a result of its ownership of the
Corporation’s capital stock, that is material to any Proponent individually, or to the Proponents in
the aggregate) in such business of any Proponent; and (B) the information required by Section 5(b)
(iv).

(iii)

To be timely, the written notice required by Section 5(b)(i) or 5(b)(ii)
must  be  received  by  the  Secretary  of  the  Corporation  at  the  principal  executive  offices  of  the
Corporation  not  later  than  the  close  of  business  on  the  ninetieth  (90th)  day  nor  earlier  than  the
close  of  business  on  the  one  hundred  twentieth  (120th)  day  prior  to  the  first  anniversary  of  the
preceding  year’s  annual  meeting;  provided,  however,  that,  subject  to  the  last  sentence  of  this
Section 5(b)(iii), in the event that no annual meeting was held during the preceding year or the date
of  the  annual  meeting  is  advanced  more  than  thirty  (30)  days  prior  to  or  delayed  by  more  than
thirty  (30)  days  after  the  anniversary  of  the  preceding  year’s  annual  meeting,  notice  by  the
stockholder  to  be  timely  must  be  so  received  not  earlier  than  the  close  of  business  on  the  one
hundred twentieth (120th) day prior to such annual meeting and not later than the close of business
on the later of the ninetieth (90th) day prior to such annual meeting or the closing of business on
the tenth (10th) day following the day on which public announcement of the date of such meeting
is first made.  In no event shall an adjournment or a postponement of an annual meeting for which
notice has been given, or the public announcement thereof has been made, commence a new time
period (or extend any time period) for the giving of a stockholder’s notice as described above.

(iv)

The  written  notice  required  by  Section  5(b)(i)  or  5(b)(ii)  shall  also
set forth, as of the date of the notice and as to the stockholder giving the notice and the beneficial
owner,  if  any,  on  whose  behalf  the  nomination  or  proposal  is  made  (each,  a  “Proponent”  and
collectively, the “Proponents”):  (A) the name and address of each Proponent, as they appear on
the  Corporation’s  books;  (B)  the  class,  series  and  number  of  shares  of  the  Corporation  that  are
owned  beneficially  and  of  record  by  each  Proponent;  (C)  a  description  of  any  agreement,
arrangement  or  understanding  (whether  oral  or  in  writing)  with  respect  to  such  nomination  or
proposal  between  or  among  any  Proponent  and  any  of  its  affiliates  or  associates,  and  any  others
(including  their  names)  acting  in  concert,  or  otherwise  under  the  agreement,  arrangement  or
understanding, with any of the foregoing; (D) a representation that the Proponents are holders of
record or beneficial owners, as the case may be, of shares of the Corporation entitled to vote at the
meeting  and  intend  to  appear  in  person  or  by  proxy  at  the  meeting  to  nominate  the  person  or
persons  specified  in  the  notice  (with  respect  to  a  notice  under  Section  5(b)(i))  or  to  propose  the
business  that  is  specified  in  the  notice  (with  respect  to  a  notice  under  Section  5(b)(ii));  (E)  a
representation as to whether the Proponents intend to deliver a proxy statement and form of proxy
to  holders  of  a  sufficient  number  of  holders  of  the  Corporation’s  voting  shares  to  elect  such
nominee  or  nominees  (with  respect  to  a  notice  under  Section  5(b)(i))  or  to  carry  such  proposal
(with  respect  to  a  notice  under  Section  5(b)(ii));  (F)  to  the  extent  known  by  any  Proponent,  the
name  and  address  of  any  other  stockholder  supporting  the  proposal  on  the  date  of  such
stockholder’s  notice;  and  (G)  a  description  of  all  Derivative  Transactions  (as  defined  below)  by
each  Proponent  during  the  previous  twelve  (12)  month  period,  including  the  date  of  the
transactions and the class, series and number of securities involved in, and the material economic
terms of, such Derivative Transactions.

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(c)

A  stockholder  providing  written  notice  required  by  Section  5(b)(i)  or  (ii)
shall update and supplement such notice in writing, if necessary, so that the information provided
or  required  to  be  provided  in  such  notice  is  true  and  correct  in  all  material  respects  as  of  (i)  the
record date for the meeting and (ii) the date that is five (5) business days prior to the meeting and,
in  the  event  of  any  adjournment  or  postponement  thereof,  five  (5)  business  days  prior  to  such
adjourned or postponed meeting.  In the case of an update and supplement pursuant to clause (i) of
this Section 5(c), such update and supplement shall be received by the Secretary of the Corporation
at the principal executive offices of the Corporation not later than five (5) business days after the
record date for the meeting.  In the case of an update and supplement pursuant to clause (ii) of this
Section 5(c), such update and supplement shall be received by the Secretary of the Corporation at
the principal executive offices of the Corporation not later than two (2) business days prior to the
date  for  the  meeting,  and,  in  the  event  of  any  adjournment  or  postponement  thereof,  two  (2)
business days prior to such adjourned or postponed meeting.

(d)

Notwithstanding  anything  in  Section  5(b)(iii)  to  the  contrary,  in  the  event
that the number of directors in an Expiring Class (as defined below) is increased and there is no
public  announcement  of  the  appointment  of  a  director  to  such  class,  or,  if  no  appointment  was
made, of the vacancy in such class, made by the Corporation at least ten (10) days before the last
day  a  stockholder  may  deliver  a  notice  of  nomination  in  accordance  with  Section  5(b)(iii),  a
stockholder’s  notice  required  by  this  Section  5  and  which  complies  with  the  requirements  in
Section  5(b)(i),  other  than  the  timing  requirements  in  Section  5(b)(iii),  shall  also  be  considered
timely, but only with respect to nominees for any new positions in such Expiring Class created by
such increase, if it shall be received by the Secretary of the Corporation at the principal executive
offices of the Corporation not later than the close of business on the tenth (10th) day following the
day  on  which  such  public  announcement  is  first  made  by  the  Corporation.    For  purposes  of  this
section, an “Expiring Class” shall  mean  a  class  of  directors  whose  term  shall  expire  at  the  next
annual meeting of stockholders.

(e)

A person shall not be eligible for election or re-election as a director unless
the person is nominated either in accordance with clause (ii) of Section 5(a), or in accordance with
clause (iii) of Section 5(a).  Except as otherwise required by law, the chairperson of the meeting
shall have the power and duty to determine whether a nomination or any business proposed to be
brought  before  the  meeting  was  made,  or  proposed,  as  the  case  may  be,  in  accordance  with  the
procedures  set  forth  in  these  Bylaws  and,  if  any  proposed  nomination  or  business  is  not  in
compliance  with  these  Bylaws,  or  the  Proponent  does  not  act  in  accordance  with  the
representations in Sections 5(b)(iv)(D) and 5(b)(iv)(E), to declare that such proposal or nomination
shall  not  be  presented  for  stockholder  action  at  the  meeting  and  shall  be  disregarded,
notwithstanding  that  proxies  in  respect  of  such  nominations  or  such  business  may  have  been
solicited or received.

(f)

Notwithstanding  the  foregoing  provisions  of  this  Section  5,  in  order  to
include  information  with  respect  to  a  stockholder  proposal  in  the  proxy  statement  and  form  of
proxy  for  a  stockholders’  meeting,  a  stockholder  must  also  comply  with  all  applicable
requirements of the 1934 Act and the rules and regulations thereunder.  Nothing in these Bylaws
shall  be  deemed  to  affect  any  rights  of  stockholders  to  request  inclusion  of  proposals  in  the
Corporation’s proxy statement pursuant to Rule 14a-8 under the 1934 Act; provided, however, that
any references in these Bylaws to the 1934 Act or the rules and regulations thereunder are not

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intended to and shall not limit the requirements applicable to proposals and/or nominations to be
considered pursuant to Section 5(a)(iii) of these Bylaws.

(g)

For purposes of Sections 5 and 6,

Rule 405 under the Securities Act of 1933, as amended (the “1933 Act”).

(i)

“affiliates”  and  “associates”  shall  have  the  meanings  set  forth  in

“Derivative  Transaction”  means  any  agreement,  arrangement,
interest or understanding entered into by, or on behalf or for the benefit of, any Proponent or any of
its affiliates or associates, whether record or beneficial:

(ii)

the  value  of  which  is  derived  in  whole  or  in  part  from  the  value  of  any  class  or

(w)
series of shares or other securities of the Corporation,

which otherwise provides any direct or indirect opportunity to gain or share in any

(x)
gain derived from a change in the value of securities of the Corporation,

the effect or intent of which is to mitigate loss, manage risk or benefit of security

(y)
value or price changes, or

(z)
which provides the right to vote or increase or decrease the voting power of, such
Proponent,  or  any  of  its  affiliates  or  associates,  with  respect  to  any  securities  of  the
Corporation,

which  agreement,  arrangement,  interest  or  understanding  may  include,  without  limitation,  any
option,  warrant,  debt  position,  note,  bond,  convertible  security,  swap,  stock  appreciation  right,
short position, profit interest, hedge, right to dividends, voting agreement, performance-related fee
or arrangement to borrow or lend shares (whether or not subject to payment, settlement, exercise or
conversion  in  any  such  class  or  series),  and  any  proportionate  interest  of  such  Proponent  in  the
securities  of  the  Corporation  held  by  any  general  or  limited  partnership,  or  any  limited  liability
company,  of  which  such  Proponent  is,  directly  or  indirectly,  a  general  partner  or  managing
member.

(iii)

“public  announcement”  shall  mean  disclosure  in  a  press  release
reported  by  the  Dow  Jones  News  Service,  Associated  Press,  Business  Wire,  GlobeNewswire  or
comparable  national  news  service  or  in  a  document  publicly  filed  by  the  Corporation  with  the
Securities and Exchange Commission pursuant to Section 13, 14 or 15(d) of the 1934 Act; and

Section 6.

Special Meetings.

(a)

Special meetings of the stockholders of the Corporation may be called, for
any  purpose  as  is  a  proper  matter  for  stockholder  action  under  Delaware  law,  by  (i)  the
Chairperson of the Board  of  Directors,  (ii)  the  Chief  Executive  Officer  if  the  Chairperson of the
Board of Directors is unavailable, or (iii) the Board of Directors pursuant to a resolution adopted
by a majority of the total number of authorized directors (whether or not there exist any vacancies
in previously authorized directorships at the time any such resolution is presented to the Board of
Directors for adoption).

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(b)

The  Board  of  Directors  shall  determine  the  time  and  place,  if  any,  of  such
special meeting.  Upon determination of the time and place, if any, of the meeting, the Secretary of
the Corporation shall cause a notice of meeting to be given to the stockholders entitled to vote, in
accordance with the provisions of Section 7 of these Bylaws.  No business may be transacted at
such special meeting other than specified in the notice of meeting.

(c)

Nominations of persons for election to the Board of Directors may be made
at a special meeting of stockholders at which directors are to be elected (i) by or at the direction of
the Board of Directors or (ii) by any stockholder of the Corporation who is a stockholder of record
at  the  time  of  giving  notice  provided  for  in  this  paragraph,  who  shall  be  entitled  to  vote  at  the
meeting  and  who  delivers  written  notice  to  the  Secretary  of  the  Corporation  setting  forth  the
information required by Section 5(b) (i).  In the event the Corporation calls a special meeting of
stockholders for the purpose of electing one or more directors to the Board of Directors, any such
stockholder of record may nominate a person or persons (as the case may be), for election to such
position(s)  as  specified  in  the  Corporation’s  notice  of  meeting,  if  written  notice  setting  forth  the
information required by Section 5(b)(i) of these Bylaws shall be received by the Secretary of the
Corporation  at  the  principal  executive  offices  of  the  Corporation  not  later  than  the  close  of
business  on  the  later  of  the  ninetieth  (90th)  day  prior  to  such  meeting  or  the  tenth  (10th)  day
following the day on which public announcement is first made of the date of the special meeting
and  of  the  nominees  proposed  by  the  Board  of  Directors  to  be  elected  at  such  meeting.    The
stockholder shall also update and supplement such information as required under Section 5(c).  In
no event shall an adjournment or a postponement of a special meeting for which notice has been
given, or the public  announcement  thereof  has  been  made,  commence  a  new  time period for the
giving of a stockholder’s notice as described above.

(d)

Notwithstanding  the  foregoing  provisions  of  this  Section  6,  a  stockholder
must also comply with all applicable requirements of the 1934 Act and the rules and regulations
thereunder  with  respect  to  matters  set  forth  in  this  Section  6.    Nothing  in  these  Bylaws  shall  be
deemed to affect any rights of stockholders to request inclusion of proposals in the Corporation’s
proxy statement pursuant to Rule 14a-8 under the 1934 Act; provided, however, that any references
in  these  Bylaws  to  the  1934  Act  or  the  rules  and  regulations  thereunder  are  not  intended  to  and
shall not limit the requirements applicable to nominations for the election to the Board of Directors
to be considered pursuant to Section 6(c) of these Bylaws.

Section 7.

Notice of Meetings.  Except as otherwise provided by law, notice, given in
writing or by electronic transmission, of each meeting of stockholders shall be given not less than
ten (10) nor more than sixty (60) days before the date of the meeting to each stockholder entitled to
vote at such meeting, such notice to specify the place, if any, date and hour, in the case of special
meetings,  the  purpose  or  purposes  of  the  meeting,  and  the  means  of  remote  communications,  if
any, by which stockholders and proxy holders may be deemed to be present in person and vote at
any  such  meeting.    If  mailed,  notice  is  given  when  deposited  in  the  United  States  mail,  postage
prepaid, directed to the stockholder at such stockholder’s address as it appears on the records of the
Corporation.  Notice of the time, place, if any, and purpose of any meeting of stockholders may be
waived in writing, signed by the person entitled to notice thereof, or by electronic transmission by
such person, either before or after such meeting, and will be waived by any stockholder by his or
her  attendance  thereat  in  person,  by  remote  communication,  if  applicable,  or  by  proxy,  except
when the stockholder attends a meeting for the express purpose of objecting, at

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the beginning of the meeting, to the transaction of any business because the meeting is not lawfully
called  or  convened.   Any  stockholder  so  waiving  notice  of  such  meeting  shall  be  bound  by  the
proceedings of any such meeting in all respects as if due notice thereof had been given.

Section 8.

Quorum.  At all meetings of stockholders, except where otherwise provided
by statute or by the Amended and Restated Certificate of Incorporation, or by these Bylaws, the
presence, in person, by remote communication, if applicable, or by proxy duly authorized, of the
holders of a majority of the voting power of the outstanding shares of stock entitled to vote shall
constitute a quorum for the transaction of business.  In the absence of a quorum, any meeting of
stockholders may be adjourned, from time to time, either by the chairperson of the meeting or by
vote of the holders of a majority of the voting power of the shares represented thereat, but no other
business  shall  be  transacted  at  such  meeting.    The  stockholders  present  at  a  duly  called  or
convened  meeting,  at  which  a  quorum  is  present,  may  continue  to  transact  business  until
adjournment, notwithstanding the withdrawal of enough stockholders to leave less than a quorum.
 Except as otherwise provided by statute or by applicable stock exchange rules, or by the Amended
and Restated Certificate of Incorporation or these Bylaws, in all matters other than the election of
directors, the affirmative vote of the majority of voting power of the shares present in person, by
remote communication, if applicable, or represented by proxy at the meeting and entitled to vote
generally on the subject matter shall be the act of the stockholders.  Except as otherwise provided
by  statute  or  by  applicable  stock  exchange  rules,  the  Amended  and  Restated  Certificate  of
Incorporation or these Bylaws, directors shall be elected by a plurality of the votes of the shares
present in person, by remote communication, if applicable, or represented by proxy at the meeting
and  entitled  to  vote  generally  on  the  election  of  directors.    Where  a  separate  vote  by  a  class  or
classes or series is required, except where otherwise provided by the statute, or by applicable stock
exchange rules, or by the Amended and Restated Certificate of Incorporation or these Bylaws, a
majority of the voting power of the outstanding shares of such class or classes or series, present in
person,  by  remote  communication,  if  applicable,  or  represented  by  proxy  duly  authorized,  shall
constitute a quorum entitled to take action with respect to that vote on that matter.  Except where
otherwise  provided  by  statute  or  by  applicable  stock  exchange  rules  or  by  the  Amended  and
Restated  Certificate  of  Incorporation  or  these  Bylaws,  the  affirmative  vote  of  the  majority
(plurality, in the case of the election of directors) of shares of such class or classes or series present
in person, by remote communication, if applicable, or represented by proxy at the meeting shall be
the act of such class or classes or series.

Section 9.

Adjournment  and  Notice  of  Adjourned  Meetings.    Any  meeting  of
stockholders,  whether  annual  or  special,  may  be  adjourned  from  time  to  time  either  by  the
chairperson of the meeting or by the vote of a majority of the voting power of the shares present in
person, by remote communication, if applicable, or represented by proxy at the meeting.  When a
meeting  is  adjourned  to  another  time  or  place,  if  any,  notice  need  not  be  given  of  the  adjourned
meeting  if  the  time  and  place,  if  any,  thereof  are  announced  at  the  meeting  at  which  the
adjournment is taken.  At the adjourned meeting, the Corporation may transact any business which
might have been transacted at the original meeting.  If the adjournment is for more than thirty (30)
days or if after the adjournment a new record date is fixed for the adjourned meeting, a notice of
the adjourned meeting shall be given to each stockholder of record entitled to vote at the meeting.

Section 10. Voting Rights.  For the purpose of determining those stockholders entitled

to vote at any meeting of the stockholders, except as otherwise provided by law, only persons in

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whose names shares stand on the stock records of the Corporation on the record date, as provided
in  Section  12  of  these  Bylaws,  shall  be  entitled  to  vote  at  any  meeting  of  stockholders.    Every
person entitled to vote shall have the right to do so either in person, by remote communication, if
applicable, or by an agent or agents authorized by a proxy granted in accordance with Delaware
law.   An  agent  so  appointed  need  not  be  a  stockholder.    No  proxy  shall  be  voted  after  three  (3)
years from its date of creation unless the proxy provides for a longer period.

Section 11.

Joint Owners of Stock.    If  shares  or  other  securities  having  voting  power
stand  of  record  in  the  names  of  two  (2)  or  more  persons,  whether  fiduciaries,  members  of  a
partnership, joint tenants, tenants in common, tenants by the entirety, or otherwise, or if two (2) or
more persons have the same fiduciary relationship respecting the same shares, unless the Secretary
of  the  Corporation  is  given  written  notice  to  the  contrary  and  is  furnished  with  a  copy  of  the
instrument or order appointing them or creating the relationship wherein it is so provided, their acts
with respect to voting shall have the following effect:  (a) if only one (1) votes, his or her act binds
all; (b) if more than one (1) votes, the act of the majority so voting binds all; (c) if more than one
(1) votes, but the vote is evenly split on any particular matter, each faction may vote the securities
in question proportionally, or may apply to the Delaware Court of Chancery for relief as provided
in the DGCL, Section 217(b).  If the instrument filed with the Secretary of the Corporation shows
that  any  such  tenancy  is  held  in  unequal  interests,  a  majority  or  even-split  for  the  purpose  of
subsection (c) of Section 11 shall be a majority or even-split in interest.

Section 12.

List of Stockholders.   The  Secretary  of  the  Corporation  shall  prepare  and
make,  at  least  ten  (10)  days  before  every  meeting  of  stockholders,  a  complete  list  of  the
stockholders entitled to vote at said meeting, arranged in alphabetical order, showing the address of
each stockholder and the number and class of shares registered in the name of each stockholder.
  Such  list  shall  be  open  to  the  examination  of  any  stockholder,  for  any  purpose  germane  to  the
meeting, (a) on a reasonably accessible electronic network, provided that the information required
to  gain  access  to  such  list  is  provided  with  the  notice  of  the  meeting,  or  (b)  during  ordinary
business  hours,  at  the  principal  place  of  business  of  the  Corporation.    In  the  event  that  the
Corporation determines to make the list available on an electronic network, the Corporation may
take  reasonable  steps  to  ensure  that  such  information  is  available  only  to  stockholders  of  the
Corporation.    The  list  shall  be  open  to  examination  of  any  stockholder  during  the  time  of  the
meeting as provided by law.

Section 13. Action  Without  Meeting.    No  action  shall  be  taken  by  the  stockholders
except at an annual or special meeting of stockholders called in accordance with these Bylaws, and
no action shall be taken by the stockholders by written consent or by electronic transmission.

Section 14. Organization.

(a)

At every meeting of stockholders, the Chairperson of the Board of Directors,
or, if a Chairperson has not been appointed or is absent, the Chief Executive Officer, or if no Chief
Executive  Officer  is  then  serving  or  is  absent,  the  President,  or,  if  the  President  is  absent,  a
chairperson  of  the  meeting  chosen  by  a  majority  in  interest  of  the  stockholders  entitled  to  vote,
present in person or by proxy, shall act as chairperson.  The Chairperson of the Board may appoint
the Chief Executive Officer as chairperson of the meeting.  The Secretary of the Corporation, or, in
his or her absence, an Assistant Secretary of the Corporation or other officer or

26

other  person  directed  to  do  so  by  the  chairperson  of  the  meeting,  shall  act  as  secretary  of  the
meeting.

(b)

The  Board  of  Directors  of  the  Corporation  shall  be  entitled  to  make  such
rules  or  regulations  for  the  conduct  of  meetings  of  stockholders  as  it  shall  deem  necessary,
appropriate or convenient.  Subject to such rules and regulations of the Board of Directors, if any,
the chairperson of the meeting shall have the right and authority to prescribe such rules, regulations
and  procedures  and  to  do  all  such  acts  as,  in  the  judgment  of  such  chairperson,  are  necessary,
appropriate  or  convenient  for  the  proper  conduct  of  the  meeting,  including,  without  limitation,
establishing an agenda or order of business for the meeting, rules and procedures for maintaining
order at the meeting and the safety of those present, limitations on participation in such meeting to
stockholders  of  record  of  the  Corporation  and  their  duly  authorized  and  constituted  proxies  and
such  other  persons  as  the  chairperson  shall  permit,  restrictions  on  entry  to  the  meeting  after  the
time  fixed  for  the  commencement  thereof,  limitations  on  the  time  allotted  to  questions  or
comments by participants and regulation of the opening and closing of the polls for balloting on
matters which are to be voted on by ballot.  The date and time of the opening and closing of the
polls for each matter upon which the stockholders will vote at the meeting shall be announced at
the meeting.  Unless and to the extent determined by the Board of Directors or the chairperson of
the meeting, meetings of stockholders shall not be required to be held in accordance with rules of
parliamentary procedure.

ARTICLE IV

DIRECTORS

Section 15. Number  and  Term  of  Office.   The  authorized  number  of  directors  of  the
Corporation  shall  be  fixed  in  accordance  with  the  Amended  and  Restated  Certificate  of
Incorporation.    Directors  need  not  be  stockholders  unless  so  required  by  the  Amended  and
Restated Certificate of Incorporation.  If for any cause, the directors shall not have been elected at
an annual meeting, they may be elected as soon thereafter as convenient at a special meeting of the
stockholders called for that purpose in the manner provided in these Bylaws.

Section 16.

Powers.  The business and affairs of the Corporation shall be managed by or
under the direction of the Board of Directors, except as may be otherwise provided by statute or by
the Amended and Restated Certificate of Incorporation.

Section 17. Classes of Directors.

Subject  to  the  rights  of  the  holders  of  any  series  of  Preferred  Stock  to  elect  additional
directors  under  specified  circumstances,  following  the  closing  of  the  initial  public  offering
pursuant to an effective registration statement under the 1933 Act, covering the offer and sale of
Common Stock of the Corporation to the public (the “Initial Public Offering”), the directors shall
be divided into three classes designated as Class I, Class II and Class III, respectively.  The Board
of  Directors  is  authorized  to  assign  members  of  the  Board  of  Directors  already  in  office  to  such
classes at the time the classification becomes effective.  At the first annual meeting of stockholders
following the closing of the Initial Public Offering, the term of office of the Class I directors shall
expire and Class I directors shall be elected for a full term of three years.  At the second annual

26

meeting of stockholders following the closing of the Initial Public Offering, the term of office of
the  Class  II  directors  shall  expire  and  Class  II  directors  shall  be  elected  for  a  full  term  of  three
years.    At  the  third  annual  meeting  of  stockholders  following  the  closing  of  the  Initial  Public
Offering, the term of office of the Class III directors shall expire and Class III directors shall be
elected for a full term of three years.  At each succeeding annual meeting of stockholders, directors
shall  be  elected  for  a  full  term  of  three  years  to  succeed  the  directors  of  the  class  whose  terms
expire at such annual meeting.

Notwithstanding the foregoing provisions of this Section 17, each director shall serve until
his  or  her  successor  is  duly  elected  and  qualified  or  until  his  or  her  earlier  death,  resignation  or
removal.  No decrease in the number of directors constituting the Board of Directors shall shorten
the term of any incumbent director.

Section 18. Vacancies.

Unless otherwise provided in the Amended and Restated Certificate of Incorporation, and
subject  to  the  rights  of  the  holders  of  any  series  of  Preferred  Stock  or  as  otherwise  provided  by
applicable  law,  any  vacancies  on  the  Board  of  Directors  resulting  from  death,  resignation,
disqualification,  removal  or  other  causes  and  any  newly  created  directorships  resulting  from  any
increase in the number of directors shall, unless the Board of Directors determines by resolution
that  any  such  vacancies  or  newly  created  directorships  shall  be  filled  by  stockholders,  be  filled
only by the affirmative vote of a majority of the directors then in office, even though less than a
quorum  of  the  Board  of  Directors,  or  by  a  sole  remaining  director,  and  not  by  the  stockholders,
provided, however, that whenever the holders of any class or classes of stock or series thereof are
entitled to elect one or more directors by the provisions of the Amended and Restated Certificate of
Incorporation,  vacancies  and  newly  created  directorships  of  such  class  or  classes  or  series  shall,
unless the Board of Directors determines by resolution that any such vacancies or newly created
directorships shall be filled by stockholders, be filled by a majority of the directors elected by such
class or classes or series thereof then in office, or by a sole remaining director so elected, and not
by  the  stockholders.   Any  director  elected  in  accordance  with  the  preceding  sentence  shall  hold
office  for  the  remainder  of  the  full  term  of  the  director  for  which  the  vacancy  was  created  or
occurred and until such director’s successor shall have been elected and qualified.

A vacancy in the Board of Directors shall be deemed to exist under this Bylaw in the case

of the death, removal or resignation of any director.

Section 19. Resignation.  Any director may resign at any time by delivering his or her
notice in writing or by electronic transmission to the Secretary of the Corporation, such resignation
to  specify  whether  it  will  be  effective  at  a  particular  time.    If  no  such  specification  is  made,  the
resignation shall be deemed effective at the time of delivery of the resignation to the Secretary of
the Corporation.  When one or more directors shall resign from the Board of Directors, effective at
a future date, a majority of the directors then in office, including those who have so resigned, shall
have power to fill such vacancy or vacancies, the vote thereon to take effect when such resignation
or  resignations  shall  become  effective,  and  each  director  so  chosen  shall  hold  office  for  the
unexpired  portion  of  the  term  of  the  director  whose  place  shall  be  vacated  and  until  his  or  her
successor shall have been duly elected and qualified.

26

Section 20. Removal.  Subject to any limitation imposed by law, any individual director
or directors may be removed with cause by the affirmative vote of the holders of at least sixty-six
and two-thirds percent (66 2/3%) of the voting power of all then outstanding shares of capital stock
of the Corporation entitled to vote generally at an election of directors, voting together as a single
class.

Section 21. Meetings.

(a)

Regular  Meetings.    Unless  otherwise  restricted  by  the  Amended  and
Restated  Certificate  of  Incorporation,  regular  meetings  of  the  Board  of  Directors  may  be  held  at
any  time  or  date  and  at  any  place  within  or  without  the  State  of  Delaware  which  has  been
designated by the Board of Directors and publicized among all directors, either orally or in writing,
by  telephone,  including  a  voice-messaging  system  or  other  system  designed  to  record  and
communicate  messages,  facsimile,  telegraph  or  telex,  or  by  electronic  mail  or  other  electronic
means.  No further notice shall be required for regular meetings of the Board of Directors.

(b)

Special  Meetings.    Unless  otherwise  restricted  by  the  Amended  and
Restated  Certificate  of  Incorporation,  special  meetings  of  the  Board  of  Directors  may  be  held  at
any time and place within or without the State of Delaware whenever called by the Chairperson of
the Board, the Chief Executive Officer or a majority of the total number of authorized directors.

(c)

Meetings  by  Electronic  Communications  Equipment.    Any  member  of
the  Board  of  Directors,  or  of  any  committee  thereof,  may  participate  in  a  meeting  by  means  of
conference  telephone  or  other  communications  equipment  by  means  of  which  all  persons
participating in the meeting can hear each other, and participation in a meeting by such means shall
constitute presence in person at such meeting.

(d)

Notice  of  Special  Meetings.    Notice  of  the  time  and  place  of  all  special
meetings  of  the  Board  of  Directors  shall  be  orally  or  in  writing,  by  telephone,  including  a  voice
messaging system or other system or technology designed to record and communicate messages,
facsimile,  telegraph  or  telex,  or  by  electronic  mail  or  other  electronic  means,  during  normal
business hours, at least twenty-four (24) hours before the date and time of the meeting.  If notice is
sent by U.S. mail, it shall be sent by first class mail, charges prepaid, at least three (3) days before
the  date  of  the  meeting.    Notice  of  any  meeting  may  be  waived  in  writing,  or  by  electronic
transmission,  at  any  time  before  or  after  the  meeting  and  will  be  waived  by  any  director  by
attendance  thereat,  except  when  the  director  attends  the  meeting  for  the  express  purpose  of
objecting, at the beginning of the meeting, to the transaction of any business because the meeting is
not lawfully called or convened.

(e) Waiver  of  Notice.    The  transaction  of  all  business  at  any  meeting  of  the
Board of Directors, or any committee thereof, however called or noticed, or wherever held, shall
be as valid as though it had been transacted at a meeting duly held after regular call and notice, if a
quorum be present and if, either before or after the meeting, each of the directors not present who
did  not  receive  notice  shall  sign  a  written  waiver  of  notice  or  shall  waive  notice  by  electronic
transmission.   All  such  waivers  shall  be  filed  with  the  corporate  records  or  made  a  part  of  the
minutes of the meeting.

26

Section 22. Quorum and Voting.

(a)

Unless  the  Amended  and  Restated  Certificate  of  Incorporation  requires  a
greater  number,  and  except  with  respect  to  questions  related  to  indemnification  arising  under
Section 44 for which a quorum shall be one-third of the exact number of directors fixed from time
to  time,  a  quorum  of  the  Board  of  Directors  shall  consist  of  a  majority  of  the  exact  number  of
directors fixed from time to time by the Board of Directors in accordance with the Amended and
Restated  Certificate  of  Incorporation;  provided,  however,  at  any  meeting  whether  a  quorum  be
present or otherwise, a majority of the directors present may adjourn from time to time until the
time  fixed  for  the  next  regular  meeting  of  the  Board  of  Directors,  without  notice  other  than  by
announcement at the meeting.

(b)

At each meeting of the Board of Directors at which a quorum is present, all
questions and business shall be determined by the affirmative vote of a majority of the directors
present,  unless  a  different  vote  be  required  by  law,  the  Amended  and  Restated  Certificate  of
Incorporation or these Bylaws.

Section 23. Action Without Meeting.  Unless otherwise restricted by the Amended and
Restated Certificate of Incorporation or these Bylaws, any action required or permitted to be taken
at  any  meeting  of  the  Board  of  Directors  or  of  any  committee  thereof  may  be  taken  without  a
meeting,  if  all  members  of  the  Board  of  Directors  or  committee,  as  the  case  may  be,  consent
thereto  in  writing  or  by  electronic  transmission,  and  such  writing  or  writings  or  transmission  or
transmissions  are  filed  with  the  minutes  of  proceedings  of  the  Board  of  Directors  or  committee.
  Such  filing  shall  be  in  paper  form  if  the  minutes  are  maintained  in  paper  form  and  shall  be  in
electronic form if the minutes are maintained in electronic form.

Section 24.

Fees and Compensation.  Directors shall be entitled to such compensation
for  their  services  as  may  be  approved  by  the  Board  of  Directors,  including,  if  so  approved,  by
resolution of the Board of Directors, a fixed sum and expenses of attendance, if any, for attendance
at each regular or special meeting of the Board of Directors and at any meeting of a committee of
the Board of Directors.  Nothing herein contained shall be construed to preclude any director from
serving  the  Corporation  in  any  other  capacity  as  an  officer,  agent,  employee,  or  otherwise  and
receiving compensation therefor.

Section 25. Committees.

(a)

Executive Committee.  The Board of Directors may designate an Executive
Committee  to  consist  of  one  (1)  or  more  members  of  the  Board  of  Directors.    The  Executive
Committee, to the extent permitted by law and provided in the resolution of the Board of Directors
shall  have  and  may  exercise  all  the  powers  and  authority  of  the  Board  of  Directors  in  the
management  of  the  business  and  affairs  of  the  Corporation,  and  may  authorize  the  seal  of  the
Corporation to be affixed to all papers which may require it; but no such committee shall have the
power or authority in reference to (i) approving or adopting, or recommending to the stockholders,
any  action  or  matter  (other  than  the  election  or  removal  of  directors)  expressly  required  by  the
DGCL to be submitted to stockholders for approval, or (ii) adopting, amending or repealing any
Bylaw of the Corporation.

26

(b)

Other  Committees.    The  Board  of  Directors  may,  from  time  to  time,
designate such other committees as may be permitted by law.  Such other committees designated
by the Board of Directors shall consist of one (1) or more members of the Board of Directors and
shall  have  such  powers  and  perform  such  duties  as  may  be  prescribed  by  the  resolution  or
resolutions creating such committees, but in no event shall any such committee have the power or
authority  in  reference  to  (i)  approving  or  adopting,  or  recommending  to  the  stockholders,  any
action or matter (other than the election or removal of directors) expressly required by the DGCL
to be submitted to stockholders for approval, or (ii) adopting, amending or repealing any Bylaw of
the Corporation.

(c)

Term.    The  Board  of  Directors,  subject  to  any  requirements  of  any
outstanding series of Preferred Stock and the provisions of subsections (a) or (b) of this Section 25,
may  at  any  time  increase  or  decrease  the  number  of  members  of  a  committee  or  terminate  the
existence of a committee.  The membership of a committee member shall terminate on the date of
his or her death or voluntary resignation from the committee or from the Board of Directors.  The
Board of Directors may at any time for any reason remove any individual committee member and
the Board of Directors may fill any committee vacancy created by death, resignation, removal or
increase in the number of members of the committee.  The Board of Directors may designate one
or  more  directors  as  alternate  members  of  any  committee,  who  may  replace  any  absent  or
disqualified  member  at  any  meeting  of  the  committee,  and,  in  addition,  in  the  absence  or
disqualification  of  any  member  of  a  committee,  the  member  or  members  thereof  present  at  any
meeting  and  not  disqualified  from  voting,  whether  or  not  he  or  they  constitute  a  quorum,  may
unanimously appoint another member of the Board of Directors to act at the meeting in the place
of any such absent or disqualified member.

(d) Meetings.    Unless  the  Board  of  Directors  shall  otherwise  provide,  regular
meetings of the Executive Committee or any other committee designated pursuant to this Section
25 shall be held at such times and places as are determined by the Board of Directors, or by any
such committee, and when notice thereof has been given to each member of such committee, no
further  notice  of  such  regular  meetings  need  be  given  thereafter.    Special  meetings  of  any  such
committee  may  be  held  at  any  place  which  has  been  determined  from  time  to  time  by  such
committee, and may be called by any director who is a member of such committee, upon notice to
the members of such committee of the time and place of such special meeting given in the manner
provided for the giving of notice to members of the Board of Directors of the time and place of
special meetings of the Board of Directors.  Notice of any special meeting of any committee may
be waived in writing or by electronic transmission at any time before or after the meeting and will
be  waived  by  any  director  by  attendance  thereat,  except  when  the  director  attends  such  special
meeting for the express purpose of objecting, at the beginning of the meeting, to the transaction of
any business because the meeting is not lawfully called or convened.  Unless otherwise provided
by the Board of Directors in the resolutions authorizing the creation of the committee, a majority
of  the  authorized  number  of  members  of  any  such  committee  shall  constitute  a  quorum  for  the
transaction  of  business,  and  the  act  of  a  majority  of  those  present  at  any  meeting  at  which  a
quorum  is  present  shall  be  the  act  of  such  committee.    Unless  the  Board  of  Directors  shall
otherwise provide, each committee shall conduct its business in the same manner as the Board of
Directors conducts its business pursuant to Article IV of these Bylaws.

26

Section 26. Duties of Chairperson of the Board of Directors and Lead Independent

Director.

(a)

The Chairperson of the Board of Directors, if appointed and when present,
shall preside at all meetings of the stockholders and the Board of Directors.  The Chairperson of
the Board of Directors shall perform other duties commonly incident to the office and shall also
perform such other duties and have such other powers, as the Board of Directors shall designate
from time to time.

(b)

The  Chairperson  of  the  Board  of  Directors,  or  if  the  Chairperson  is  not  an
independent  director,  one  of  the  independent  directors,  may  be  designated  by  the  Board  of
Directors  as  lead  independent  director  to  serve  until  replaced  by  the  Board  of  Directors  (“Lead
Independent Director”).  The Lead Independent Director will perform such other duties as may be
established or delegated by the Board of Directors.

Section 27. Organization.    At  every  meeting  of  the  directors,  the  Chairperson  of  the
Board of Directors, or, if a Chairperson has not been appointed or is absent, the Lead Independent
Director,  or  if  the  Lead  Independent  Director  has  not  been  appointed  or  is  absent,  the  Chief
Executive  Officer  (if  a  director),  or,  if  a  Chief  Executive  Officer  is  absent,  the  President  (if  a
director),  or  if  the  President  is  absent,  the  most  senior  Vice  President  (if  a  director),  or,  in  the
absence  of  any  such  person,  a  chairperson  of  the  meeting  chosen  by  a  majority  of  the  directors
present, shall preside over the meeting.  The Secretary of the Corporation, or in his or her absence,
any Assistant Secretary of the Corporation or other officer, director or other person directed to do
so by the person presiding over the meeting, shall act as secretary of the meeting.

ARTICLE V

OFFICERS

Section 28. Officers Designated.  The officers of the Corporation shall include, if and
when designated by the Board of Directors, the Chief Executive Officer, the President, one or more
Vice  Presidents,  the  Secretary,  the  Chief  Financial  Officer  and  the  Treasurer.    The  Board  of
Directors  may  also  appoint  one  or  more  Assistant  Secretaries  and  Assistant  Treasurers  and  such
other  officers  and  agents  with  such  powers  and  duties  as  it  shall  deem  necessary.   The  Board  of
Directors  may  assign  such  additional  titles  to  one  or  more  of  the  officers  as  it  shall  deem
appropriate.  Any one person may hold any number of offices of the Corporation at any one time
unless  specifically  prohibited  therefrom  by  law.    The  salaries  and  other  compensation  of  the
officers of the Corporation shall be fixed by or in the manner designated by the Board of Directors.

Section 29.

Tenure and Duties of Officers.

(a)

General.    All  officers  shall  hold  office  at  the  pleasure  of  the  Board  of
Directors  and  until  their  successors  shall  have  been  duly  elected  and  qualified,  unless  sooner
removed.  Any officer elected or appointed by the Board of Directors may be removed at any time
by the Board of Directors.  If the office of any officer becomes vacant for any reason, the vacancy
may be filled by the Board of Directors.

26

(b)

Duties  of  Chief  Executive  Officer.    The  Chief  Executive  Officer  shall
preside  at  all  meetings  of  the  stockholders  and  at  all  meetings  of  the  Board  of  Directors  (if  a
director), unless the Chairperson of the Board of Directors or the Lead Independent Director has
been appointed and is present.  Unless an officer has been appointed Chief Executive Officer of the
Corporation, the President shall be the chief executive officer of the Corporation and shall, subject
to  the  control  of  the  Board  of  Directors,  have  general  supervision,  direction  and  control  of  the
business  and  officers  of  the  Corporation.   To  the  extent  that  a  Chief  Executive  Officer  has  been
appointed  and  no  President  has  been  appointed,  all  references  in  these  Bylaws  to  the  President
shall  be  deemed  references  to  the  Chief  Executive  Officer.    The  Chief  Executive  Officer  shall
perform other duties commonly incident to the office and shall also perform such other duties and
have such other powers, as the Board of Directors shall designate from time to time.

(c)

Duties  of  President.    The  President  shall  preside  at  all  meetings  of  the
stockholders and at all meetings of the Board of Directors (if a director), unless the Chairperson of
the  Board  of  Directors,  the  Lead  Independent  Director  or  the  Chief  Executive  Officer  has  been
appointed and is present.  Unless another officer has been appointed Chief Executive Officer of the
Corporation, the President shall be the chief executive officer of the Corporation and shall, subject
to  the  control  of  the  Board  of  Directors,  have  general  supervision,  direction  and  control  of  the
business  and  officers  of  the  Corporation.    The  President  shall  perform  other  duties  commonly
incident to the office and shall also perform such other duties and have such other powers, as the
Board of Directors shall designate from time to time.

(d)

Duties of Vice Presidents.  A Vice President may assume and perform the
duties  of  the  President  in  the  absence  or  disability  of  the  President  or  whenever  the  office  of
President is vacant.  A Vice President shall perform other duties commonly incident to their office
and shall also perform such other duties and have such other powers as the Board of Directors or
the Chief Executive Officer, or, if the Chief Executive Officer has not been appointed or is absent,
the President shall designate from time to time.

(e)

Duties  of  Secretary.    The  Secretary  of  the  Corporation  shall  attend  all
meetings  of  the  stockholders  and  of  the  Board  of  Directors  and  shall  record  all  acts  and
proceedings thereof in the minute book of the Corporation.  The Secretary of the Corporation shall
give notice in conformity with these Bylaws of all meetings of the stockholders and of all meetings
of  the  Board  of  Directors  and  any  committee  thereof  requiring  notice.    The  Secretary  of  the
Corporation shall perform all other duties provided for in these Bylaws and other duties commonly
incident to the office and shall also perform such other duties and have such other powers, as the
Board of Directors shall designate from time to time.  The Chief Executive Officer, or if no Chief
Executive  Officer  is  then  serving,  the  President  may  direct  any  Assistant  Secretary  of  the
Corporation or other officer to assume and perform the duties of the Secretary in the absence or
disability  of  the  Secretary,  and  each  Assistant  Secretary  of  the  Corporation  shall  perform  other
duties  commonly  incident  to  the  office  and  shall  also  perform  such  other  duties  and  have  such
other  powers  as  the  Board  of  Directors  or  the  Chief  Executive  Officer,  or  if  no  Chief  Executive
Officer is then serving, the President shall designate from time to time.

(f)

Duties of Chief Financial Officer.  The Chief Financial Officer shall keep
or cause to be kept the books of account of the Corporation in a thorough and proper manner and
shall render statements of the financial affairs of the Corporation in such form and as often as

26

required by the Board of Directors or the Chief Executive Officer, or if no Chief Executive officer
is  then  serving,  the  President.   The  Chief  Financial  Officer,  subject  to  the  order  of  the  Board  of
Directors,  shall  have  the  custody  of  all  funds  and  securities  of  the  Corporation.    The  Chief
Financial Officer shall perform other duties commonly incident to the office and shall also perform
such  other  duties  and  have  such  other  powers  as  the  Board  of  Directors  or  the  Chief  Executive
Officer, or if no Chief Executive Officer is then serving, the President shall designate from time to
time.  To the extent that a Chief Financial Officer has been appointed and no Treasurer has been
appointed, all references in these Bylaws to the Treasurer shall be deemed references to the Chief
Financial Officer.  The President may direct the Treasurer, if any, or any Assistant Treasurer, or the
controller  or  any  assistant  controller  to  assume  and  perform  the  duties  of  the  Chief  Financial
Officer in the absence or disability of the Chief Financial Officer, and each Treasurer and Assistant
Treasurer and each controller and assistant controller shall perform other duties commonly incident
to the office and shall also perform such other duties and have such other powers as the Board of
Directors  or  the  Chief  Executive  Officer,  or  if  no  Chief  Executive  Officer  is  then  serving,  the
President shall designate from time to time.

(g)

Duties  of  Treasurer.    Unless  another  officer  has  been  appointed  Chief
Financial  Officer  of  the  Corporation,  the  Treasurer  shall  be  the  chief  financial  officer  of  the
Corporation  and  shall  keep  or  cause  to  be  kept  the  books  of  account  of  the  Corporation  in  a
thorough and proper manner and shall render statements of the financial affairs of the Corporation
in such form and as often as required by the Board of Directors or the Chief Executive Officer, or
if no Chief Executive Officer is then serving, the President, and, subject to the order of the Board
of Directors, shall have the custody of all funds and securities of the Corporation.  The Treasurer
shall perform other duties commonly incident to the office and shall also perform such other duties
and have such other powers as the Board of Directors or the Chief Executive Officer, or if no Chief
Executive Officer is then serving, the President and the Chief Financial Officer (if not Treasurer)
shall designate from time to time.

Section 30. Delegation of Authority.    The  Board  of  Directors  may  from  time  to  time
delegate  the  powers  or  duties  of  any  officer  to  any  other  officer  or  agent,  notwithstanding  any
provision hereof.

Section 31. Resignations.    Any  officer  may  resign  at  any  time  by  giving  notice  in
writing or by electronic transmission to the Board of Directors or to the Chief Executive Officer, or
if no Chief Executive Officer is then serving, the President or to the Secretary of the Corporation.
 Any  such  resignation  shall  be  effective  when  received  by  the  person  or  persons  to  whom  such
notice is given, unless a later time is specified therein, in which event the resignation shall become
effective at such later time.  Unless otherwise specified in such notice, the acceptance of any such
resignation shall not be necessary to make it effective.  Any resignation shall be without prejudice
to the rights, if any, of the Corporation under any contract with the resigning officer.

Section 32. Removal.  Any officer may be removed from office at any time, either with
or without cause, by the affirmative vote of a majority of the directors in office at the time, or by
the unanimous written consent of the directors in office at the time, or by any committee or by the
Chief Executive Officer or by other superior officers upon whom such power of removal may have
been conferred by the Board of Directors.

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ARTICLE VI

EXECUTION OF CORPORATE INSTRUMENTS AND VOTING OF SECURITIES
OWNED BY THE CORPORATION

Section 33.

Execution of Corporate Instruments.  The Board of Directors may, in its
discretion, determine the method and designate the signatory officer or officers, or other person or
persons, to execute on behalf of the Corporation any corporate instrument or document, or to sign
on behalf of the Corporation  the  corporate  name  without  limitation,  or  to  enter into contracts on
behalf  of  the  Corporation,  except  where  otherwise  provided  by  law  or  these  Bylaws,  and  such
execution or signature shall be binding upon the Corporation.

All  checks  and  drafts  drawn  on  banks  or  other  depositaries  on  funds  to  the  credit  of  the
Corporation or in special accounts of the Corporation shall be signed by such person or persons as
the Board of Directors shall authorize so to do.

Unless authorized or ratified by the Board of Directors or within the agency power of an
officer, no officer, agent or employee shall have any power or authority to bind the Corporation by
any contract or engagement or to pledge its credit or to render it liable for any purpose or for any
amount.

Section 34. Voting  of  Securities  Owned  By  the  Corporation.    All  stock  and  other
securities of other Corporations owned or held by the Corporation for itself, or for other parties in
any capacity, shall be voted, and all proxies with respect thereto shall be executed, by the person
authorized  so  to  do  by  resolution  of  the  Board  of  Directors,  or,  in  the  absence  of  such
authorization,  by  the  Chairperson  of  the  Board  of  Directors,  the  Chief  Executive  Officer,  the
President, or any Vice President.

ARTICLE VII

SHARES OF STOCK

Section 35.

Form and Execution of Certificates.  The shares of the Corporation shall
be represented by certificates, or shall be uncertificated if so provided by resolution or resolutions
of the Board of Directors.  Certificates for the shares of stock, if any, shall be in such form as is
consistent with the Amended and Restated Certificate of Incorporation and applicable law.  Every
holder of stock in the Corporation represented by certificate shall be entitled to have a certificate
signed  by  or  in  the  name  of  the  Corporation  by  any  two  authorized  officers  of  the  Corporation,
including but not limited to, the Chief Executive Officer, the President, the Chief Financial Officer,
any  Vice  President,  the  Treasurer  or  Assistant  Treasurer  or  the  Secretary  or  Assistant  Secretary,
certifying the number of shares owned by him in the Corporation.  Any or all of the signatures on
the certificate may be facsimiles.  In case any officer, transfer agent, or registrar who has signed or
whose facsimile signature has been placed upon a certificate shall have ceased to be such officer,
transfer agent, or registrar before such certificate is issued, it may be issued with the same effect as
if he were such officer, transfer agent, or registrar at the date of issue.

Section 36.

Lost Certificates.  A new certificate or certificates shall be issued in place

of any certificate or certificates theretofore issued by the Corporation alleged to have been lost,

26

stolen,  or  destroyed,  upon  the  making  of  an  affidavit  of  that  fact  by  the  person  claiming  the
certificate of stock to be lost, stolen, or destroyed.  The Corporation may require, as a condition
precedent  to  the  issuance  of  a  new  certificate  or  certificates,  the  owner  of  such  lost,  stolen,  or
destroyed certificate or certificates, or the owner’s legal representative, to agree to indemnify the
Corporation  in  such  manner  as  it  shall  require  or  to  give  the  Corporation  a  surety  bond  in  such
form  and  amount  as  it  may  direct  as  indemnity  against  any  claim  that  may  be  made  against  the
Corporation with respect to the certificate alleged to have been lost, stolen, or destroyed.

Section 37.

Transfers.

(a)

Transfers of record of shares of stock of the Corporation shall be made only
upon its books by the holders thereof, in person or by attorney duly authorized, and, in the case of
stock represented by certificate, upon the surrender of a properly endorsed certificate or certificates
for a like number of shares.

(b)

The Corporation shall have power to enter into and perform any agreement
with any number of stockholders of any one or more classes of stock of the Corporation to restrict
the  transfer  of  shares  of  stock  of  the  Corporation  of  any  one  or  more  classes  owned  by  such
stockholders in any manner not prohibited by the DGCL.

Section 38.

Fixing Record Dates.

(a)

In  order  that  the  Corporation  may  determine  the  stockholders  entitled  to
notice  of  or  to  vote  at  any  meeting  of  stockholders  or  any  adjournment  thereof,  the  Board  of
Directors  may  fix  a  record  date,  which  record  date  shall  not  precede  the  date  upon  which  the
resolution fixing the record date is adopted by the Board of Directors, and which record date shall,
subject to applicable law, not be more than sixty (60) nor less than ten (10) days before the date of
such meeting.  If no record date is fixed by the Board of Directors, the record date for determining
stockholders  entitled  to  notice  of  or  to  vote  at  a  meeting  of  stockholders  shall  be  at  the  close  of
business on the day next preceding the day on which notice is given, or if notice is waived, at the
close of business on the day next preceding the day on which the meeting is held.  A determination
of stockholders of record entitled to notice of or to vote at a meeting of stockholders shall apply to
any  adjournment  of  the  meeting;  provided,  however,  that  the  Board  of  Directors  may  fix  a  new
record date for the adjourned meeting.

(b)

In  order  that  the  Corporation  may  determine  the  stockholders  entitled  to
receive payment of any dividend or other distribution or allotment of any rights or the stockholders
entitled to exercise any rights in respect of any change, conversion or exchange of stock, or for the
purpose  of  any  other  lawful  action,  the  Board  of  Directors  may  fix,  in  advance,  a  record  date,
which  record  date  shall  not  precede  the  date  upon  which  the  resolution  fixing  the  record  date  is
adopted, and which record date shall be not more than sixty (60) days prior to such action.  If no
record date is fixed, the record date for determining stockholders for any such purpose shall be at
the  close  of  business  on  the  day  on  which  the  Board  of  Directors  adopts  the  resolution  relating
thereto.

Section 39. Registered  Stockholders.    The  Corporation  shall  be  entitled  to  recognize

the exclusive right of a person registered on its books as the owner of shares to receive dividends,

26

and to vote as such owner, and shall not be bound to recognize any equitable or other claim to or
interest in such share or shares on the part of any other person whether or not it shall have express
or other notice thereof, except as otherwise provided by the laws of Delaware.

ARTICLE VIII

OTHER SECURITIES OF THE CORPORATION

Section 40.

Execution of Other Securities.  All bonds, debentures and other corporate
securities of the Corporation, other than stock certificates (covered in Section 35), may be signed
by the Chief Executive Officer, the President or any Vice President, or such other person as may be
authorized by the Board of Directors, and if such securities require it, the corporate seal may be
impressed  thereon  or  a  facsimile  of  such  seal  may  be  imprinted  thereon  and  attested  by  the
signature of the Secretary of the Corporation or an Assistant Secretary of the Corporation, or the
Chief Financial Officer or Treasurer or an Assistant Treasurer; provided, however, that where any
such bond, debenture or other corporate security shall be authenticated by the manual signature, or
where  permissible  facsimile  signature,  of  a  trustee  under  an  indenture  pursuant  to  which  such
bond, debenture or other corporate security shall be issued, the signatures of the persons signing
and  attesting  the  corporate  seal  on  such  bond,  debenture  or  other  corporate  security  may  be  the
imprinted facsimile of the signatures of such persons.  Interest coupons appertaining to any such
bond, debenture or other corporate security, authenticated by a trustee as aforesaid, shall be signed
by  the  Treasurer  or  an  Assistant  Treasurer  of  the  Corporation  or  such  other  person  as  may  be
authorized  by  the  Board  of  Directors,  or  bear  imprinted  thereon  the  facsimile  signature  of  such
person.    In  case  any  officer  who  shall  have  signed  or  attested  any  bond,  debenture  or  other
corporate  security,  or  whose  facsimile  signature  shall  appear  thereon  or  on  any  such  interest
coupon, shall have ceased to be such officer before the bond, debenture or other corporate security
so signed or attested shall have been delivered, such bond, debenture or other corporate security
nevertheless  may  be  adopted  by  the  Corporation  and  issued  and  delivered  as  though  the  person
who signed the same or whose facsimile signature shall have been used thereon had not ceased to
be such officer of the Corporation.

ARTICLE IX

DIVIDENDS

Section 41. Declaration  of  Dividends.    Dividends  upon  the  capital  stock  of  the
Corporation,  subject  to  the  provisions  of  the  Amended  and  Restated  Certificate  of  Incorporation
and  applicable  law,  if  any,  may  be  declared  by  the  Board  of  Directors  pursuant  to  law  at  any
regular or special meeting.  Dividends may be paid in cash, in property, or in shares of the capital
stock,  subject  to  the  provisions  of  the  Amended  and  Restated  Certificate  of  Incorporation  and
applicable law.

Section 42. Dividend Reserve.  Before payment of any dividend, there may be set aside
out  of  any  funds  of  the  Corporation  available  for  dividends  such  sum  or  sums  as  the  Board  of
Directors  from  time  to  time,  in  their  absolute  discretion,  think  proper  as  a  reserve  or  reserves  to
meet contingencies, or for equalizing dividends, or for repairing or maintaining any property of the
Corporation, or for such other purpose as the Board of Directors shall think conducive to the

26

interests of the Corporation, and the Board of Directors may modify or abolish any such reserve in
the manner in which it was created.

ARTICLE X

FISCAL YEAR

Section 43.
of the Board of Directors.

Fiscal Year.  The fiscal year of the Corporation shall be fixed by resolution

ARTICLE XI

INDEMNIFICATION

Section 44.

Indemnification  of  Directors,  Executive  Officers,  Other  Officers,

Employees and Other Agents.

(a)

Directors  and  Executive  Officers.    The  Corporation  shall  indemnify  its
directors and executive officers (for the purposes of this Article XI, “executive officers” shall have
the meaning defined in Rule 3b-7 promulgated under the 1934 Act) to the extent not prohibited by
the DGCL or any other applicable law; provided, however, that  the  Corporation  may  modify  the
extent  of  such  indemnification  by  individual  contracts  with  its  directors  and  executive  officers;
and,  provided,  further,  that  the  Corporation  shall  not  be  required  to  indemnify  any  director  or
executive  officer  in  connection  with  any  proceeding  (or  part  thereof)  initiated  by  such  person
unless  (i)  such  indemnification  is  expressly  required  to  be  made  by  law,  (ii)  the  proceeding  was
authorized by the Board of Directors of the Corporation, (iii) such indemnification is provided by
the Corporation, in its sole discretion, pursuant to the powers vested in the Corporation under the
DGCL  or  any  other  applicable  law  or  (iv)  such  indemnification  is  required  to  be  made  under
subsection (d).

(b)

Other  Officers,  Employees  and  Other  Agents.    The  Corporation  shall
have power to indemnify its other officers, employees and other agents as set forth in the DGCL or
any  other  applicable  law.    The  Board  of  Directors  shall  have  the  power  to  delegate  the
determination  of  whether  indemnification  shall  be  given  to  any  such  person  except  executive
officers to such officers or other persons as the Board of Directors shall determine.

(c)

Expenses.    The  Corporation  shall  advance  to  any  person  who  was  or  is  a
party or is threatened to be made a party to any threatened, pending or completed action, suit or
proceeding, whether civil, criminal, administrative or investigative, by reason of the fact that he is
or was a director or executive officer, of the Corporation, or is or was serving at the request of the
Corporation  as  a  director  or  executive  officer  of  another  Corporation,  partnership,  joint  venture,
trust or other enterprise, prior to the final disposition of the proceeding, promptly following request
therefor,  all  expenses  incurred  by  any  director  or  executive  officer  in  connection  with  such
proceeding provided, however, that if the DGCL requires, an advancement of expenses incurred by
a director or executive officer in his or her capacity as a director or executive officer (and not in
any  other  capacity  in  which  service  was  or  is  rendered  by  such  indemnitee,  including,  without
limitation,  service  to  an  employee  benefit  plan)  shall  be  made  only  upon  delivery  to  the
Corporation of an undertaking (hereinafter an “undertaking”), by or on behalf of such indemnitee,

26

to repay all amounts so advanced if it shall ultimately be determined by final judicial decision from
which there is no further right to appeal (hereinafter a “final adjudication”) that such indemnitee is
not entitled to be indemnified for such expenses under this section or otherwise.

Notwithstanding  the  foregoing,  unless  otherwise  determined  pursuant  to  paragraph  (e)  of
this  section,  no  advance  shall  be  made  by  the  Corporation  to  an  executive  officer  of  the
Corporation  (except  by  reason  of  the  fact  that  such  executive  officer  is  or  was  a  director  of  the
Corporation  in  which  event  this  paragraph  shall  not  apply)  in  any  action,  suit  or  proceeding,
whether  civil,  criminal,  administrative  or  investigative,  if  a  determination  is  reasonably  and
promptly made (i) by a majority vote of directors who were not parties to the proceeding, even if
not  a  quorum,  or  (ii)  by  a  committee  of  such  directors  designated  by  a  majority  vote  of  such
directors, even though less than a quorum, or (iii) if there are no such directors, or such directors so
direct,  by  independent  legal  counsel  in  a  written  opinion,  that  the  facts  known  to  the  decision-
making  party  at  the  time  such  determination  is  made  demonstrate  clearly  and  convincingly  that
such  person  acted  in  bad  faith  or  in  a  manner  that  such  person  did  not  believe  to  be  in  or  not
opposed to the best interests of the Corporation.

(d)

Enforcement.  Without the necessity of entering into an express contract, all
rights to indemnification and advances to directors and executive officers under this Bylaw shall be
deemed  to  be  contractual  rights  and  be  effective  to  the  same  extent  and  as  if  provided  for  in  a
contract  between  the  Corporation  and  the  director  or  executive  officer.    Any  right  to
indemnification  or  advances  granted  by  this  section  to  a  director  or  executive  officer  shall  be
enforceable by or on behalf of the person holding such right in any court of competent jurisdiction
if (i) the claim for indemnification or advances is denied, in whole or in part, or (ii) no disposition
of such claim is made within ninety (90) days of request therefor.  To the extent permitted by law,
the claimant in such enforcement action, if successful in whole or in part, shall be entitled to be
paid also the expense of prosecuting the claim.  In connection with any claim for indemnification,
the Corporation shall be entitled to raise as a defense to any such action that the claimant has not
met the standards of conduct that make it permissible under the DGCL or any other applicable law
for  the  Corporation  to  indemnify  the  claimant  for  the  amount  claimed.    In  connection  with  any
claim by an executive officer of the Corporation (except in any action, suit or proceeding, whether
civil, criminal, administrative or investigative, by reason of the fact that such executive officer is or
was a director of the Corporation) for advances, the Corporation shall be entitled to raise a defense
as  to  any  such  action  clear  and  convincing  evidence  that  such  person  acted  in  bad  faith  or  in  a
manner  that  such  person  did  not  believe  to  be  in  or  not  opposed  to  the  best  interests  of  the
Corporation, or with respect to any criminal action or proceeding that such person acted without
reasonable  cause  to  believe  that  his  or  her  conduct  was  lawful.    Neither  the  failure  of  the
Corporation  (including  its  Board  of  Directors,  independent  legal  counsel  or  its  stockholders)  to
have made a determination prior to the commencement of such action that indemnification of the
claimant is proper in the circumstances because he has met the applicable standard of conduct set
forth  in  the  DGCL  or  any  other  applicable  law,  nor  an  actual  determination  by  the  Corporation
(including its Board of Directors, independent legal counsel or its stockholders) that the claimant
has  not  met  such  applicable  standard  of  conduct,  shall  be  a  defense  to  the  action  or  create  a
presumption that claimant has not met the applicable standard of conduct.  In any suit brought by a
director or executive officer to enforce a right to indemnification or to an advancement of expenses
hereunder, the burden of proving that the director or executive officer is not entitled to

26

be indemnified, or to such advancement of expenses, under this section or otherwise shall be on the
Corporation.

(e)

Non-Exclusivity  of  Rights.    The  rights  conferred  on  any  person  by  this
Bylaw shall not be exclusive of any other right which such person may have or hereafter acquire
under any applicable statute, provision of the Amended and Restated Certificate of Incorporation,
Bylaws, agreement, vote of stockholders or disinterested directors or otherwise, both as to action in
his  or  her  official  capacity  and  as  to  action  in  another  capacity  while  holding  office.    The
Corporation  is  specifically  authorized  to  enter  into  individual  contracts  with  any  or  all  of  its
directors,  officers,  employees  or  agents  respecting  indemnification  and  advances,  to  the  fullest
extent not prohibited by the DGCL, or by any other applicable law.

(f)

Survival of Rights.  The rights conferred on any person by this Bylaw shall
continue as to a person who has ceased to be a director, officer, employee or other agent and shall
inure to the benefit of the heirs, executors and administrators of such a person.

(g)

Insurance.    To  the  fullest  extent  permitted  by  the  DGCL  or  any  other
applicable law, the Corporation, upon approval by the Board of Directors, may purchase insurance
on behalf of any person required or permitted to be indemnified pursuant to this section.

(h)

Amendments.    Any  repeal  or  modification  of  this  section  shall  only  be
prospective  and  shall  not  affect  the  rights  under  this  Bylaw  in  effect  at  the  time  of  the  alleged
occurrence of any action or omission to act that is the cause of any proceeding against any agent of
the Corporation.

(i)

Saving Clause.  If this Bylaw or any portion hereof shall be invalidated on
any  ground  by  any  court  of  competent  jurisdiction,  then  the  Corporation  shall  nevertheless
indemnify  each  director  and  executive  officer  to  the  full  extent  not  prohibited  by  any  applicable
portion of this section that shall not have been invalidated, or by any other applicable law.  If this
section  shall  be  invalid  due  to  the  application  of  the  indemnification  provisions  of  another
jurisdiction,  then  the  Corporation  shall  indemnify  each  director  and  executive  officer  to  the  full
extent under any other applicable law.

(j)

Certain  Definitions.    For  the  purposes  of  this  Bylaw,  the  following

definitions shall apply:

(i)

The term “proceeding” shall be broadly construed and shall include,
without limitation, the investigation, preparation, prosecution, defense, settlement, arbitration and
appeal  of,  and  the  giving  of  testimony  in,  any  threatened,  pending  or  completed  action,  suit  or
proceeding, whether civil, criminal, administrative or investigative.

(ii)

The  term  “expenses”  shall  be  broadly  construed  and  shall  include,
without limitation, court costs, attorneys’ fees, witness fees, fines, amounts paid in settlement or
judgment and any other costs and expenses of any nature or kind incurred in connection with any
proceeding.

Corporation, any constituent Corporation (including any constituent of a constituent)

(iii)

The term the “Corporation” shall include, in addition to the resulting

26

absorbed in a consolidation or merger which, if its separate existence had continued, would have
had power and authority to indemnify its directors, officers, and employees or agents, so that any
person who is or was a director, officer, employee or agent of such constituent Corporation, or is or
was serving at the request of such constituent Corporation as a director, officer, employee or agent
of another Corporation, partnership, joint venture, trust or other enterprise, shall stand in the same
position under the provisions of this section with respect to the resulting or surviving Corporation
as  he  would  have  with  respect  to  such  constituent  Corporation  if  its  separate  existence  had
continued.

(iv)

References 

to  a  “director,”  “executive  officer,”  “officer,”
“employee,” or “agent” of the Corporation shall include, without limitation, situations where such
person  is  serving  at  the  request  of  the  Corporation  as,  respectively,  a  director,  executive  officer,
officer, employee, trustee or agent of another Corporation, partnership, joint venture, trust or other
enterprise.

(v)

References  to  “other  enterprises”  shall  include  employee  benefit
plans; references to “fines” shall include any excise taxes assessed on a person with respect to an
employee benefit plan; and references to “serving at the request of the Corporation” shall include
any service as a director, officer, employee or agent of the Corporation which imposes duties on, or
involves services by, such director, officer, employee, or agent with respect to an employee benefit
plan,  its  participants,  or  beneficiaries;  and  a  person  who  acted  in  good  faith  and  in  a  manner  he
reasonably  believed  to  be  in  the  interest  of  the  participants  and  beneficiaries  of  an  employee
benefit plan shall be deemed to have acted in a manner “not opposed to the best interests of the
Corporation” as referred to in this section.

ARTICLE XII

NOTICES

Section 45. Notices.

(a)

Notice  to  Stockholders.    Written  notice  to  stockholders  of  stockholder
meetings  shall  be  given  as  provided  in  Section  7  herein.   Without  limiting  the  manner  by  which
notice  may  otherwise  be  given  effectively  to  stockholders  under  any  agreement  or  contract  with
such  stockholder,  and  except  as  otherwise  required  by  law,  written  notice  to  stockholders  for
purposes  other  than  stockholder  meetings  may  be  sent  by  U.S.  mail  or  nationally  recognized
overnight  courier,  or  by  facsimile,  telegraph  or  telex  or  by  electronic  mail  or  other  electronic
means.

(b)

Notice to Directors.  Any notice required to be given to any director may be
given by the method stated in subsection (a), or as otherwise provided in these Bylaws, with notice
other than one which is delivered personally to be sent to such address as such director shall have
filed in writing with the Secretary of the Corporation, or, in the absence of such filing, to the last
known address of such director.

(c)

Affidavit  of  Mailing.    An  affidavit  of  mailing,  executed  by  a  duly
authorized and competent employee of the Corporation or its transfer agent appointed with respect
to the class of stock affected, or other agent, specifying the name and address or the names and

26

addresses of the stockholder or stockholders, or director or directors, to whom any such notice or
notices  was  or  were  given,  and  the  time  and  method  of  giving  the  same,  shall  in  the  absence  of
fraud, be prima facie evidence of the facts therein contained.

(d) Methods  of  Notice.    It  shall  not  be  necessary  that  the  same  method  of
giving notice be employed in respect of all recipients of notice, but one permissible method may be
employed  in  respect  of  any  one  or  more,  and  any  other  permissible  method  or  methods  may  be
employed in respect of any other or others.

(e)

Notice  to  Person  With  Whom  Communication  is  Unlawful.    Whenever
notice  is  required  to  be  given,  under  any  provision  of  law  or  of  the  Amended  and  Restated
Certificate  of  Incorporation  or  Bylaws  of  the  Corporation,  to  any  person  with  whom
communication is unlawful, the giving of such notice to such person shall not be required and there
shall be no duty to apply to any governmental authority or agency for a license or permit to give
such notice to such person.  Any action or meeting which shall be taken or held without notice to
any such person with whom communication is unlawful shall have the same force and effect as if
such notice had been duly given.  In the event that the action taken by the Corporation is such as to
require  the  filing  of  a  certificate  under  any  provision  of  the  DGCL,  the  certificate  shall  state,  if
such  is  the  fact  and  if  notice  is  required,  that  notice  was  given  to  all  persons  entitled  to  receive
notice except such persons with whom communication is unlawful.

(f)

Notice  to  Stockholders  Sharing  an  Address.    Except  as  otherwise
prohibited  under  DGCL,  any  notice  given  under  the  provisions  of  DGCL,  the  Amended  and
Restated Certificate of Incorporation or these Bylaws shall be effective if given by a single written
notice to stockholders who share an address if consented to by the stockholders at that address to
whom  such  notice  is  given.    Such  consent  shall  have  been  deemed  to  have  been  given  if  such
stockholder fails to object in writing to the Corporation within sixty (60) days of having been given
notice by the Corporation of its intention to send the single notice.  Any consent shall be revocable
by the stockholder by written notice to the Corporation.

ARTICLE XIII

AMENDMENTS

Section 46.

[  ].  Subject to the limitations set forth in Section 44(h) of these Bylaws or
the provisions of the Amended and Restated Certificate of Incorporation, the Board of Directors is
expressly empowered to adopt, amend or repeal these Bylaws of the Corporation.  Any adoption,
amendment or repeal of these Bylaws of the Corporation by the Board of Directors shall require
the approval of a majority of the authorized number of directors.  The stockholders also shall have
power  to  adopt,  amend  or  repeal  these  Bylaws  of  the  Corporation;  provided,  however,  that,  in
addition to any vote of the holders of any class or series of stock of the Corporation required by
law or by the Amended and Restated Certificate of Incorporation, such action by stockholders shall
require the affirmative vote of the holders of at least sixty-six and two-thirds percent (66-2/3%) of
the  voting  power  of  all  of  the  then-outstanding  shares  of  the  capital  stock  of  the  Corporation
entitled to vote generally in the election of directors, voting together as a single class.

26

ARTICLE XIV

LOANS TO OFFICERS

Section 47.

Loans to Officers.    Except  as  otherwise  prohibited  by  applicable  law,  the
Corporation may lend money to, or guarantee any obligation of, or otherwise assist any officer or
other employee of the Corporation or of its subsidiaries, including any officer or employee who is
a  director  of  the  Corporation  or  its  subsidiaries,  whenever,  in  the  judgment  of  the  Board  of
Directors,  such  loan,  guarantee  or  assistance  may  reasonably  be  expected  to  benefit  the
Corporation.  The loan, guarantee or other assistance may be with or without interest and may be
unsecured, or secured in such manner as the Board of Directors shall approve, including, without
limitation,  a  pledge  of  shares  of  stock  of  the  Corporation.    Nothing  in  these  Bylaws  shall  be
deemed to deny, limit or restrict the powers of guaranty or warranty of the Corporation at common
law or under any statute.

ARTICLE XV

EXCLUSIVE FORUM PROVISIONS

Section 48.

Federal  Forum  Selection.    Unless  the  Corporation  consents  in  writing  to
the selection of an alternative forum (an “Alternative Forum Consent”), the federal district courts
of  the  United  States  of  America  shall,  to  the  fullest  extent  permitted  by  law,  be  the  sole  and
exclusive forum for the resolution of any complaint asserting a cause of action arising under the
1933 Act.  Any person or entity purchasing, holding, owning or otherwise acquiring any interest in
any security of the Corporation shall be deemed to have notice of and consented to the provisions
of this Section 48.  The existence of any prior Alternative Forum Consent shall not act as a waiver
of the Corporation’s ongoing consent right as set forth above in this Section 48 with respect to any
current or future actions or claims arising under the 1933 Act.

26

CERTIFICATION OF AMENDED AND RESTATED BYLAWS
OF
APPLIED THERAPEUTICS, INC.

a Delaware Corporation

I,  Shoshana  Shendelman,  certify  that  I  am  the  Secretary  of  Applied  Therapeutics,  Inc.,  a
Delaware  corporation  (the  “Corporation”),  that  I  am  duly  authorized  to  make  and  deliver  this
certification, that the attached Amended and Restated Bylaws are a true and complete copy of the
Amended and Restated Bylaws of the Corporation in effect as of the date of this certificate.

Dated:  March 16, 2021

/s/ Shoshana Shendelman
Shoshana Shendelman, Ph.D.
Secretary

26

  
 
CERTAIN  IDENTIFIED  INFORMATION  HAS  BEEN  EXCLUDED  FROM  THIS
EXHIBIT  BECAUSE  IT  IS  NOT  MATERIAL  AND  IS  THE  TYPE  OF  INFORMATION
THAT  THE  REGISTRANT  CUSTOMARILY  AND  ACTUALLY  TREATS  AS  PRIVATE
[***]  INDICATES  THAT  INFORMATION  HAS  BEEN
AND  CONFIDENTIAL. 
REDACTED.

Exhibit 10.9

EXCLUSIVE LICENSE AND SUPPLY AGREEMENT

by and between

APPLIED THERAPEUTICS, INC.

and

MERCURY PHARMA GROUP LIMITED

January 3, 2023

TABLE OF CONTENTS

SECTION 1. DEFINITIONS
SECTION 2. LICENSE
SECTION 3. ALLIANCE MANAGERS
SECTION 4. DEVELOPMENT
SECTION 5. REGULATORY AFFAIRS
SECTION 6. PRICING AND MARKET ACCESS
SECTION 7. COMMERCIALIZATION
SECTION 8. MANUFACTURE AND SUPPLY
SECTION 9. FINANCIAL PROVISIONS
SECTION 10. ACCOUNTING AND PROCEDURES FOR PAYMENT
SECTION 11. PATENTS AND INFRINGEMENT
SECTION 12. CONFIDENTIALITY; PUBLICATION
SECTION 13. WARRANTIES
SECTION 14. NON-COMPETITION
SECTION 15. TERM
SECTION 16. TERMINATION
SECTION 17. INDEMNIFICATION, INSURANCE AND LIABILITY
SECTION 18. GOVERNING LAW AND JURISDICTION
SECTION 19. MISCELLANEOUS

i

1
16
21
22
23
26
27
32
41
43
45
49
51
53
53
54
61
64
66

EXCLUSIVE LICENSE AND SUPPLY AGREEMENT

This Exclusive License and Supply Agreement (this “Agreement”) dated as of January 3,
2023 is made by and between Applied Therapeutics, Inc., a company organized and existing under
the laws of the State of Delaware in the U.S. with its head office at 545 5th Ave Suite 1400, New
York,  NY  10017  (“Applied”),  and  Mercury  Pharma  Group  Limited  (trading  as  Advanz  Pharma
Holdings), a company organized and existing under the laws of England and Wales with its head
office  at  Capital  House,  85  King  William  Street,  London,  EC4N  7BL,  United  Kingdom  and
registered under number 02330913 (“Advanz”) (each, a “Party” and collectively, the “Parties”).

WHEREAS,  Applied  is  engaged  in,  among  other  things,  Developing  the  Compound  and

the Product and owns or otherwise controls certain Patent Rights and Technology relating thereto;

WHEREAS,  Advanz  has  experience  and  expertise  in  the  marketing  and  selling  of
pharmaceutical products, and desires to acquire the licenses set out in this Agreement including an
exclusive license in  the  Territory  to  Commercialize  the  Product  in  the  Field,  upon the terms and
subject to the conditions set forth herein; and

WHEREAS, Applied desires to grant such license to Advanz.

NOW,  THEREFORE,  in  consideration  of  the  mutual  covenants  and  agreements  provided

herein, Applied and Advanz hereby agree as follows:

SECTION 1. DEFINITIONS

For purposes of this Agreement, the following definitions shall be applicable:

1.1

“Acquiror  Assets”  means,  with  respect  to  Patent  Rights  or  Technology  (and  all
Intellectual  Property  (other  than  Patent  Rights)  therein),  as  applicable,  such  Patent  Rights  or
Technology  (and  all  Intellectual  Property  (other  than  Patent  Rights)  therein)  owned  or  otherwise
Controlled by the Acquiror Group other than:

(a)

any  Patent  Rights  or  Technology  (and  all  Intellectual  Property  (other  than  Patent
Rights) therein) the Control of which is transferred from Applied and or its Affiliates (other than
the Acquiror Group) to the Acquiror Group;

(b)

any improvements, enhancements, modifications and updates to (a); and

(c)

any  Patent  Rights  and  Technology  (and  Intellectual  Property  (other  than  Patent
Rights)  therein)  owned  or  Controlled  by  the  Acquiror  Group  access  to  which  is  provided  to
Applied or any of its Affiliates (other than the Acquiror Group),

each to the extent necessary or useful for the Exploitation of the Compound or Product in the Field
in the Territory and which are “Applied Patent Rights”  or “Applied Technology” as appropriate.

1.2

“Acquiror Group” means a Third Party acquiror of Applied or any Affiliate of such

acquiror (other than Applied or any Affiliate controlled (as defined in Section 1.10) by Applied).

18

1.3

“Additional Indication”  means  (a)  an  Indication  for  the  Product  outside  the  Field;
and  (b)  solely  to  the  extent  for  one  of  the  Licensed  Indications,  any  of  Applied’s  products  other
than the Product.

1.4

“Additional  Indication  Notice”  shall  have  the  meaning  assigned  to  it  in

Section 2.5(a).

1.5

“Advanz” shall have the meaning assigned to it in the Preamble.

1.6

“Advanz  Confidential  Information”  means  all  information  or  data,  including
proprietary  information  and  materials,  relating  to  the  business,  operations,  Technology,
Commercialization, Development and Manufacturing activities of Advanz (including sales data of
Advanz  and  any  information  of  Advanz  created  under  or  in  connection  with  this  Agreement  by
Advanz), whether in oral, written, graphic, machine-readable form, or any other form, disclosed or
made available by or on behalf of Advanz to Applied, Applied’s Affiliates, or its or their respective
directors, officers, employees, consultants, contractors or agents or otherwise acquired by any such
Persons  as  a  result  of  or  in  connection  with  this  Agreement  or  the  Parties’  discussions  (whether
prior to the execution hereof or thereafter).  Information will be considered Advanz Confidential
Information under this Agreement if a reasonable person, given the nature of information and the
circumstances of disclosure, would consider such information to be confidential.  Information shall
not  be  considered  to  be  Advanz  Confidential  Information  to  the  extent  that  such  information  is:
(a) as of the date of disclosure known to Applied or its Affiliates, as demonstrable in any tangible
medium  in  existence  at  the  time  of  disclosure;  (b)  wholly  disclosed  in  published  literature,  or
otherwise  is  or  becomes  generally  known  to  the  public  through  no  breach  by  Applied  of  this
Agreement; (c) obtained by Applied or its Affiliates from a Third Party free from any obligation of
confidentiality  to  Advanz  or  its  Affiliates;  or  (d)  independently  developed  by  Applied  or  its
Affiliates without use of or reference to the Advanz Confidential Information.

1.7

1.8

“Advanz Indemnitees” shall have the meaning assigned to it in Section 17.2.

“Advanz Recall” shall have the meaning assigned to it in Section 5.5(a).

1.9

“Advanz Regulatory Activities”  means,  with  respect  to  the  Product  for  use  in  the
Field in the Territory: (a) collaborating with Applied in accordance with Section 5.3, in connection
with  determining  regulatory  plans  and  strategies  for  the  Product  in  the  Field  in  the  Territory,
including the preparation and submission of, the Marketing Authorization Applications hereunder;
(b)  collaborating  with  Applied  in  respect  of  preparation  of  the  Marketing  Authorization
Applications  in  accordance  with  Section  5.1(b),  submitting  the  Marketing  Authorization
Applications  in  Advanz’s  name,  paying  all  associated  application  fees  and  maintaining  any
resulting  Marketing  Authorizations;  (c)  preparing  and  filing,  in  Advanz’s  name,  the  respective
local  documents  and  other 
to
Commercialization  (and  other  Exploitation  under  Advanz’s  control  as  a  result  of  Advanz
exercising its Step-In Rights) of the Product in the Field in the Territory from and after receiving
the  Product  with  applicable  Regulatory  Authorities;  and
Marketing  Authorization  for 
(d) complying with the Advanz obligations in Section 8.2.

(including  Regulatory  Filings)  with 

respect 

filings 

18

1.10

“Affiliate”  means,  with  respect  to  a  Party,  any  Person  that,  directly  or  indirectly
through  one  or  more  intermediaries,  controls,  is  controlled  by,  or  is  under  common  control  with
such  Party,  but  for  only  so  long  as  such  control  exists.   As  used  in  this  Section  1.10,  “control”
means  (a)  to  possess,  directly  or  indirectly,  the  power  to  direct  or  cause  the  direction  of  the
management  or  policies  of  an  entity,  whether  through  ownership  of  voting  securities  or  voting
rights,  by  contract  or  otherwise;  or  (b)  direct  or  indirect  beneficial  ownership  of  more  than  fifty
percent (50%) (or such lesser percentage which is the maximum allowed to be owned by a foreign
entity  in  a  particular  jurisdiction)  of  the  voting  equity  securities  in  such  entity  and  the  terms
“controlled”  and  “controlling”  have  meanings  correlative  thereto.    In  the  case  of  Advanz,  this
definition  shall  exclude  any  entities  which  are  under  common  control  with  Advanz  solely  as  a
result  of  being  controlled  by  Nordic  Capital  branded  or  associated  investment  or  management
vehicles.

1.11

“Agreement” shall have the meaning assigned to it in the Preamble.

1.12

“Alliance Manager” shall have the meaning assigned to it in Section 3.1.

1.13

“Annual Net Sales” means Net Sales for any Calendar Year.

1.14

“Antitrust  Laws”  means  any  Applicable  Laws  having  the  purpose  or  effect  of
prohibiting, restricting or regulating monopolization, lessening of competition, or restraint of trade.

1.15

“Applicable  Laws”  means  the  applicable  provisions  of  any  and  all  national,
supranational, regional, state, and local laws, treaties, statutes, or rules, regulations, administrative
codes,  binding  guidance,  requirements  (whether  regulatory,  administrative  or  criminal,  including
all  requirements  related  to  privacy  and  anti-corruption  requirements),  ordinances,  judgments,
decrees,  directives,  injunctions,  orders,  or  permits  (including  Marketing  Authorizations  and  their
equivalents) of or from any court, Regulatory Authority, or other Governmental Authority having
jurisdiction over or related to the subject item.

1.16

“Applied” shall have the meaning assigned to it in the Preamble.

1.17

“Applied  Confidential  Information”  means  all  information  or  data  relating  to  the
Applied  Technology,  Compound  or  Product  (except  to  the  extent  this  is  Advanz  Confidential
Information) including all pre-clinical or clinical data, manufacturing processes, controls and data,
and  regulatory  dossiers,  as  well  as  any  other  information,  including  proprietary  information  and
materials,  regarding  the  business,  operations,  Technology  and  the  supply,  Manufacture,
Development,  Commercialization  and  other  Exploitation  activities  of  Applied,  whether  in  oral,
written, graphic, machine-readable form, or any other form, disclosed or made available by or on
behalf  of  Applied  to  Advanz,  Advanz’s  Affiliates,  or  its  and  their  respective  directors,  officers,
employees, consultants, contractors or agents or otherwise acquired by any such Persons as a result
of or in connection with this Agreement or the Parties’ discussions (whether prior to the execution
hereof or thereafter).  Information will be considered Applied Confidential Information under this
Agreement  if  a  reasonable  person,  given  the  nature  of  information  and  the  circumstances  of
disclosure,  would  consider  such  information  to  be  confidential.    Information  shall  not  be
considered to be Applied Confidential Information to the extent that such information is: (a) as of
the date of disclosure known to Advanz or its Affiliates, as demonstrable in any tangible medium

18

in existence at the time of disclosure; (b) wholly disclosed in published literature, or otherwise is
or  becomes  generally  known  to  the  public  through  no  breach  by  Advanz  of  this  Agreement;
(c)  obtained  by  Advanz  or  its  Affiliates  from  a  Third  Party  free  from  any  obligation  of
confidentiality to Applied or its Affiliates (including in the exercise of its rights or performance of
its obligations under this Agreement); or (d) independently developed by Advanz or its Affiliates
without use of or reference to the Applied Confidential Information.

1.18

“Applied Indemnitees” shall have the meaning assigned to it in Section 17.1.

1.19

“Applied Patent Rights” means all Patent Rights owned or otherwise Controlled by
Applied or any of its controlled Affiliates as of the Effective Date or at any time during the Term,
excluding Acquiror Assets, to the extent that they relate to the Exploitation of the Compound or
Product in the Field in the Territory (including the composition of matter, manufacture or use of
the foregoing), including the Patent Rights listed in Exhibit B, other than Patent Rights which are
Acquiror Assets.

1.20

“Applied Recall” shall have the meaning assigned to it in the Section 5.5(a).

1.21

“Applied  Technology”  means  any  Technology  and  all  Intellectual  Property  (other
than  Patent  Rights)  therein,  owned  or  otherwise  Controlled  by  Applied  or  any  of  its  controlled
Affiliates as of the Effective Date or at any time during the Term, excluding Acquiror Assets, that
is necessary or useful for the Development, Manufacture, Commercialization or other Exploitation
of the Compound or Product in the Field in the Territory, other than Technology which is Acquiror
Assets.

1.22

“Audit” shall have the meaning assigned to it in Section 10.8.

1.23

“Bulk Product” means the Product (AT-007 liquid suspension) in bulk bottle format

for supply to secondary packaging facilities identified by Advanz.

1.24

“Business Day” means a day other than a Saturday, Sunday, or bank or other public

holiday in New York, New York or London, United Kingdom.

1.25

“Calendar Quarter” means each of the four (4) three (3)-month periods commencing
on January 1 of any Calendar Year and ending on (respectively) March 31, June 30, September 30,
and December 31 of such Calendar Year.

1.26

“Calendar  Year”  means  the  twelve  (12)-month  period  commencing  on  January  1
and ending on December 31 of any calendar year; provided that the first Calendar Year of the Term
shall commence on the Effective Date and end on December 31 of such calendar year and the last
Calendar Year of the Term shall end on the date of expiration or termination of this Agreement.

1.27

“cGDP”  means  the  European  current  good  distribution  practice  standards  on  the
distribution of products, including requirements for transport, storage, distribution and wholesale
as specified by Applicable Laws of the relevant Countries at the time of distribution conducted in
accordance with this Agreement.

18

1.28

“cGMP” means the good manufacturing practice standards for methods to be used
in, and the facilities or controls to be used for, the manufacture, processing, packing, distribution or
holding  of  a  pharmaceutical  product  or  drug  substance  as  specified  by  Applicable  Laws  of  the
relevant  Countries  at  the  time  of  manufacturing  conducted  in  accordance  with  this  Agreement,
including (a) Directive 2003/94/EC; (b) Volume 4, Rules Governing Medicinal Products in the EU,
Part I and II; and (c) the Human Medicines Regulations 2012, each as amended from time to time.

1.29

“Claims” shall have the meaning assigned to it in Section 17.1.

1.30

“Columbia” shall have the meaning assigned to it in Section 1.31.

1.31

“Columbia  License”  means  that  certain  Exclusive  License  Agreement  by  and
between The Trustees of Columbia University in the City of New York (“Columbia”) and Applied,
dated October 26, 2016.

1.32

“Columbia Patents” shall have the meaning assigned to it in Section 11.1.

1.33

“Commercial  Event  Milestone  1”  shall  have  the  meaning  assigned  to  it  in

Section 9.2(a).

1.34

“Commercial  Event  Milestone  2”  shall  have  the  meaning  assigned  to  it  in

Section 9.2(a).

1.35

“Commercial  Event  Milestone  3”  shall  have  the  meaning  assigned  to  it  in

Section 9.2(a).

1.36

“Commercial  Event  Milestone  4”  shall  have  the  meaning  assigned  to  it  in

Section 9.2(a).

1.37

“Commercial  Event  Milestone  Payments”  means  the  Event  Milestone  Payments

opposite each Commercial Event Milestone, as set forth in Section 9.2(a).

1.38

“Commercial  Event  Milestones”  means  Commercial  Event  Milestone  1,
Commercial Event Milestone 2, Commercial Event Milestone 3 and Commercial Event Milestone
4.

1.39

“Commercialization”  means with respect  to  a  pharmaceutical  product,  any  and  all
activities  directed  to  the  marketing,  promotion,  importation,  labeling,  distribution,  exportation,
transport,  offering  for  sale,  sale  of  and  having  sold  such  pharmaceutical  product,  but  excluding,
Development  and  Manufacturing.    “Commercialize”  and  “Commercializing”  have  correlative
meanings.

1.40

“Commercialization Plan” shall have the meaning assigned to it in Section 7.2.

1.41

“Commercially  Reasonable  Efforts”  means  with  respect  to  the  efforts  to  be
expended  by  a  Party  with  respect  to  the  objective  that  is  the  subject  of  such  efforts,  reasonable,
good faith efforts and resources to accomplish such objective that such Party would normally use

18

to accomplish a similar objective under similar circumstances, it being understood and agreed that
such  efforts  shall  be  similar  to  those  efforts  and  resources  consistent  with  industry  practice  in
pursuing  the  Commercialization  or  other  Exploitation  (as  applicable)  of  pharmaceutical  products
for  treatment  of  rare  diseases  in  the  specialty  pharmaceutical  industry,  taking  into  account  all
relevant  factors,  including  the  orphan  drug  and  specialty  pharmaceutical  status  of  the
pharmaceutical  product  and  other  regulatory  matters,  safety  and  efficacy  matters,  labeling  or
anticipated  labeling,  pricing,  present  and  future  market  potential,  past  performance  of  the
pharmaceutical  product,  financial  return  (but  without  taking  into  account  the  Royalties  or  Event
Milestone  Payments  made  or  required  to  be  made  hereunder  in  the  case  of  Commercialization),
medical  and  clinical  considerations,  present  and  future  regulatory  environment  and  competitive
market conditions, all as measured by the facts and circumstances at the time such efforts are due

.

1.42

“Competing  Product”  means  any  pharmaceutical  product,  compound,  drug
substance or preparation for the treatment of a Licensed Indication, or that shows pharmacological
activity with respect to aldose reductase, and that is not the Product or Compound.

1.43

“Compound” 

2-(4-oxo-3-((5-(trifluoromethyl)benzo[d]thiazol-2-
yl)methyl)-3,4-dihydrothieno[3,4-d]pyridazin-1-yl)acetic acid (AT-007 with CAS registry number
 2170729-29-8) and the structure shown on Exhibit A,  also  called  govorestat,  including  all  salts,
hydrates, solvates, salts and isomers.

means 

1.44

“Confidential  Information”  means  the  Applied  Confidential  Information  or  the

Advanz Confidential Information, as applicable.

1.45

“Continuity Plan” shall have the meaning assigned to it in Section 19.17.

1.46

“Control” or “Controlled” means, with respect to any Intellectual Property, the legal
authority or right (whether by ownership, license or otherwise, but without taking into account any
rights granted by one Party to the other Party pursuant to this Agreement) of a Party to grant the
applicable  access  to,  or  license  or  sublicense  under,  such  Intellectual  Property  to  the  other  Party
pursuant  to  this  Agreement,  without  breaching  the  terms  of  any  agreement  or  other  arrangement
with a Third Party, or violating any Applicable Laws.

1.47

“Cost of Goods Sold” or “COGs” means Applied’s actual, directly attributable and
allocable  and,  where  reasonably  requested,  evidenced  internal  and  external  Costs  and  Expenses
reasonably incurred in Manufacturing Bulk Product for Advanz, including [***] directly relating
to  the  Manufacture  of  the  Product  calculated  in  accordance  with  Exhibit  I  and  including  the
components set out in Exhibit G.

1.48

“Costs  and  Expenses”  means  any  direct  internal  and  external  costs  and  expenses
that  would  normally  be  incurred  by  the  Party  by  which  they  are  incurred  under  similar
circumstances,  it  being  understood  and  agreed  that  such  costs  and  expenses  shall  be  similar  to
those costs and expenses consistent with industry practice and shall not include any extraordinary
costs.

1.49

“Country” means a generally recognized sovereign entity or regulatory jurisdiction.

18

1.50

“Cover(ed)(ing)” means, with respect to any Patent Right and the subject matter at
issue,  that,  but  for  ownership  or  a  license  granted  under  a  Valid  Claim  of  such  Patent,  the
Development, Manufacture, Commercialization or other Exploitation of the subject matter at issue
would  infringe  such  Valid  Claim,  or,  in  the  case  of  a  Patent  Application,  would  infringe  a  Valid
Claim in such Patent Application if it were to issue as a Patent.

1.51

“Damages” shall have the meaning assigned to it in Section 17.1.

1.52

“Development”  or  “Develop”  means  conducting  pre-clinical  studies  and  clinical
trials  (including  the  Required  Existing  Studies,  Required  Post-MA  Studies  and  Other  Post-
Approval  Studies,  but  excluding,  for  clarity,  PV  and  Risk  Management  Studies),  as  well  as
developing manufacturing data, processes and controls required for Marketing Authorization, and
collecting, validating and analyzing data in connection with the foregoing.

1.53

“Development  Costs”  means  any  costs,  fees  or  expenses  incurred  in  connection

with Development of the Product, as further described in Section 4.3.

1.54

“Dispute” shall have the meaning assigned to it in Section 18.3.

1.55

“Dispute Notice” shall have the meaning assigned to it in Section 18.3(a).

1.56

“Dossier”  means  the  complete  master  regulatory  dossier  in  e-CTD  format  for  the
Product  prepared  by  or  on  behalf  of  Applied  for  submission  by  Advanz  in  order  to  obtain  a
Marketing Authorization for the Product for use in the Field in the Territory.

1.57

“Early  Access  Program”  means  any  program  in  the  Territory  to  provide  patients
with the Product for use in the Field prior to Marketing Authorization and prior to Launch in any
Country  in  the  Territory.    “Early  Access  Programs”  include,  for  example,  any  named  patient
programs or compassionate use programs.

1.58

“Effective Date” means the date of this Agreement.

1.59

“EMA” means the European Medicines Agency or any successor agency thereto.

1.60

“English Courts” shall have the meaning assigned to it in Section 18.3(c)(iv).

1.61

“Estimated Cost” shall have the meaning assigned to it in Section 8.5(a)(i).

1.62

“Event Milestone” shall have the meaning assigned to it in Section 9.2(a).

1.63

“Event Milestone Payments” means the amounts set forth in Section 9.2(a) opposite

the respective Event Milestones.

1.64

“Exploit(ation)”  means  to  research,  Develop,  Manufacture,  Commercialize  or

otherwise use or dispose of.

1.65

“Facility”  means,  as  applicable,  those  facilities  used  by  or  on  behalf  of  Applied

(including by its Affiliates, licensees, sublicensees or designees) in the Manufacture or storage of

18

(a)  Compound,  (b)  Bulk  Product,  or  (c)  materials  or  services  utilized  in  the  Manufacture  of
Compound or Bulk Product

.  For the avoidance of doubt, “Facility”  includes  the  facilities  of  Applied’s  Third  Party  contract
manufacturers.

1.66

“Field” means the use of the Product for the Licensed Indications in humans.

1.67

“Financial Stability Event” shall have the meaning assigned to it in Section 19.17.

1.68

“FM Continuity Plan” shall have the meaning assigned to it in Section 19.1.

1.69

“Force Majeure Event” shall have the meaning assigned to it in Section 19.1.

1.70

“Forecast” shall have the meaning assigned to it in Section 8.4(a).

1.71

“Galactosemia”  means  the  genetic  metabolic  disorder  in  humans  resulting  in
deficiencies in enzymes in the Le Loir pathway of galactose metabolism, resulting in the inability
to convert galactose to glucose, known as of the Effective Date as “galactosemia.”

1.72

“Governmental Authority” means any court, agency, department, authority or other

instrumentality of any national, state, county, city or other political subdivision.

1.73

“IFRS”  means  international  financial  reporting  standards,  which  are  generally

accepted accounting principles.

1.74

“Indemnified Party” shall have the meaning assigned to it in Section 17.4(a).

1.75

“Indemnifying Party” shall have the meaning assigned to it in Section 17.4(a).

1.76

“Indication”  means  a  separate  and  distinct  disease,  disorder,  illness,  or  health
condition  in  humans  and  all  of  its  associated  signs,  symptoms,  stages,  or  progression  (including
precursor conditions), in each case for which a separate, or supplemental, Marketing Authorization
Application  may  be  filed.    For  clarity,  subpopulations  or  patients  with  a  primary  disease  or
condition,  however  stratified  (including  stratification  by  stages  of  progression,  particular
combinations  of  symptoms  associated  with  the  primary  disease  or  condition,  prior  treatment
courses, response to prior treatment, family history, clinical history, genotype, phenotype, or other
stratification) shall not be deemed to be separate “Indications” for the purposes of this Agreement.

1.77
Section 7.2.

“Initial  Commercialization  Plan”  shall  have  the  meaning  assigned  to  it  in

1.78

“Initial Forecast” shall have the meaning assigned to it in Section 8.4(a).

1.79

“Initial Royalty Term” means, on a Country-by-Country basis, the period beginning
on  the  Effective  Date  and  ending  on  the  later  of:  (a)  the  expiration  date  of  the  last  Valid  Claim
Covering the composition of matter of the Compound in the Territory; or (b) ten (10) years from
EMA’s grant of the Marketing Authorization for the Product.

18

1.80

“Intellectual  Property”  means  all  Patent  Rights,  Trademarks,  registered  designs,
design rights, copyrights (including rights in computer software and moral rights), domain names,
rights  in  databases  and  rights  in  data,  trade  secrets,  know-how  and  any  and  all  other  intellectual
property  and  proprietary  rights  in  any  Country  throughout  the  world,  whether  registered  or  not,
together  with  all  applications  and  registrations  therefor  and  all  renewals  and  extensions  of  such
rights or applications whether vested, contingent or future.

1.81

“Inventory Stock” shall have the meaning assigned to it in Section 8.11(a).

1.82

“IP Rights” shall have the meaning assigned to it in Section 18.2(a).

1.83

“Launch” means, on a Licensed Indication-by-Licensed Indication and Country-by-
Country basis, the first sale of the Product by Advanz or any of its Affiliates or Sublicensees to a
Third Party for end use of the Product for use in such Licensed Indication in such Country after
Marketing  Authorization  has  been  granted  with  respect  to  the  Product  for  use  in  such  Licensed
Indication  in  such  Country.    For  clarity,  clinical  trials,  so-called  “named  patient  sales,”  and
“compassionate  use  sales”  or  sales  under  Early  Access  Programs  (other  than  the  Early  Access
Program in France in accordance with Section 16.1(e)(i)(B)) shall not be construed as a “Launch”
hereunder.

1.84

“Licensed Indications” means SORD and Galactosemia.

1.85

“Licensed Trademarks” means those Trademarks that are Controlled by Applied in
the  Territory  that  are  used  or  intended  for  use  to  identify  the  Product  for  use  in  the  Field  in  the
Territory,  as  set  out  in  Exhibit  C  attached  hereto  (and  any  such  other  Trademarks  that  are
Controlled  by  Applied  in  the  Territory  that  the  Parties  agree  in  writing  after  the  Effective  Date
shall be used to identify the Product in the Territory, including pursuant to Section 7.4(b)).

1.86

“Long Range Forecast” shall have the meaning assigned to it in Section 8.4(b).

1.87

“Major Markets” means [***].

1.88

“Manufacture”  means  any  and  all  activities  related  to  making,  having  made,
production,  manufacture,  processing,  filling,  shipping  and  holding  of  any  compound  or
pharmaceutical  product,  including  process  development,  testing  method  development,  process
qualification  and  validation,  scale-up,  pre-clinical,  clinical  and  commercial  manufacture  and
analytic  development,  product  characterization,  stability  testing,  quality  assurance  and  quality
control,  but  excluding,  for  the  avoidance  of  doubt,  Secondary  Packaging  and  Release.
 “Manufactured” and “Manufacturing” have correlative meanings.

1.89

“Marketing  Authorization”  means  a  Regulatory  Approval  that  grants  the  right  to
place  a  pharmaceutical  product  on  a  market  in  the  Territory  (including  any  individual  Country
within  the  Territory).    For  the  avoidance  of  doubt,  “Marketing  Authorization”  includes  any
conditional or qualified authorization.

1.90

“Marketing  Authorization  Application”  means  an  application  for  a  Marketing

Authorization.

18

1.91

“Material Safety Issue” means Applied’s good faith and reasonably evidenced belief
that  there  is  an  unacceptable  risk  for  harm  in  humans  based  upon  the  observation  of  serious
adverse effects in humans after dosing the Product.

1.92

“MHRA” means the Medicines and Healthcare products Regulatory Agency in the

United Kingdom or any successor agency thereto.

1.93

“Miami” has the meaning assigned to it in Section 1.94.

1.94

“Miami License” means that certain Exclusive License Agreement by and between

University of Miami (“Miami”) and Applied dated as of October 28, 2020.

1.95

“Net  Sales”  means,  with  respect  to  a  Product,  the  gross  amounts  invoiced  by
Advanz or its Affiliates or Sublicensees for sale of Product to Third Parties and less the following
customary deductions, determined in accordance with IFRS and accounting standards and methods
consistently  applied  throughout  Advanz’s  organization,  to  the  extent  specifically  and  solely
allocated  to  such  Product  and  actually  and  properly  taken,  paid,  accrued,  allowed,  included  or
allocated:

[***]

1.96

“Non-Conformance  Dispute”  shall  have 

the  meaning  assigned 

to 

it 

in

Section 8.7(c).

1.97

“Notice  of  Non-Conformance”  shall  have  the  meaning  assigned  to  it  in

Section 8.7(a).

1.98

“Other Post-Approval Studies” means, with respect to the Compound or Product, in
each case, for use in the Field in the Territory, any pre-clinical or clinical studies commenced after
receipt of Marketing Authorization for such Product for such use, that are not Required Existing
Studies or Required Post-MA Studies including: (a) Phase IV studies (including health outcomes
and  health  services  utilization  research,  epidemiologic  studies,  and  health  economic  studies)  to
expand  the  clinical  knowledge  of  the  Product  in  a  post  marketing  and  real  world  setting;  (b)
clinical  studies  or  programs  for  expanded  or  compassionate  access;  and  (c)  investigator  initiated
trials.

1.99

“Out-of-Scope  Product”  means  the  Product  for  use  in  an  Indication  or  other  use
outside the Field (without limiting Advanz’s rights to any ROFO Product pursuant to Section 2.5),
a compound other than the Compound or a pharmaceutical product other than the Product.

1.100 “Party” or “Parties” shall have the meaning assigned to such terms in the Preamble.

1.101 “Patent Application” means any application for a Patent.

1.102 “Patent Challenge” shall have the meaning assigned to it in Section 2.6(a).

1.103 “Patent Rights” means Patents and Patent Applications.

18

1.104 “Patents”  means 

including  all
continuations,  continuations-in-part,  divisions,  provisionals  and  renewals,  and  letters  of  patent
granted  with  respect  to  any  of  the  foregoing,  patents  of  addition,  supplementary  protection
certificates,  registration  or  confirmation  patents  and  all  reissues,  re-examination  and  extensions
thereof.

issued  patents,  whether  U.S.  or  foreign, 

1.105 “Person”  means  an  individual,  corporation,  partnership,  company,  joint  venture,
unincorporated  organization,  limited  liability  company  or  partnership,  sole  proprietorship,
association,  bank,  trust  company  or  trust,  whether  or  not  legal  entities,  or  any  Governmental
Authority.

1.106 “Pharmacovigilance  Agreement”  shall  have  the  meaning  assigned  to  it  in

Section 5.4.

1.107 “PMAC Members” shall have the meaning assigned to it in Section 6.1(b).

1.108 “Price  Approval”  means,  in  any  Country  where  a  Governmental  Authority
authorizes  reimbursement  for,  or  approves  or  determines  pricing  for,  pharmaceutical  products,
receipt  (or,  if  required  to  make  such  authorization,  approval  or  determination  effective,
publication) of such reimbursement authorization or pricing approval or determination (as the case
may be).

1.109 “Pricing  and  Market  Access  Activities”  means,  with  respect  to  the  Product  in  the
Field in the Territory, strategy, activities and undertakings regarding: (a) pricing and price terms,
including  obtaining  and  maintaining  Price  Approvals,  negotiating  discounts,  rebates  and  other
price-related  matters  with  payors  and  purchasers  or  in  relation  to  formulary  placement  for
Products;  (b)  reimbursement  programs;  and  (c)  all  other  market  access  matters,  including
establishing  and  maintaining  relationships,  and  contracting  with  hospitals,  pharmacies,  group
purchasing organizations and healthcare insurers and other similar Third Parties.

1.110 “Pricing  and  Market  Access  Committee”  or  the  “PMAC”  shall  have  the  meaning

assigned to it in Section 6.1(a).

1.111 “Product”  means  any  pharmaceutical  product  that  contains  the  Compound,  as  the
sole active ingredient or together with one or more other active ingredients, in any dosage form,
strength or formulation.

1.112 “Product  Non-Conformance”  shall  have 

the  meaning  assigned 

to 

it 

in

Section 8.7(a).

1.113 “Product Recall” shall mean any Advanz Recall or Applied Recall.

1.114 “Product Specifications” means those Manufacturing, performance, quality-control
release, and other specifications for the Compound or Product (including Bulk Product) for use in
the Field in the Territory, which are initially as set forth in the applicable Marketing Authorization
for the Product, as such specifications may be amended from time to time pursuant to the terms of
this Agreement.

1.115 “Proposal” shall have the meaning assigned to it in Section 2.5(b).

18

1.116 “Purchase Order” shall have the meaning assigned to it in Section 8.4(a).

1.117 “PV and Risk Management Studies” means any (a) post authorization safety study
(“PASS”);  (b)  risk  management  plan  (“RMP”)  requirement  (such  as  product  safety  or  disease
registry);  and  (c)  pharmacovigilance  surveillance  activity  with  respect  to  the  Compound  or
Product, in each case, for use in the Field in the Territory, as required by any Regulatory Authority
in any Country in the Territory following receipt of a Marketing Authorization for the Product for
use in such Licensed Indication.

1.118 “Quality  Agreement”  means  the  Quality  Agreement  to  be  entered  into  between
Applied and Advanz with respect to the Bulk Product being supplied by Applied for commercial
supply to Advanz under the terms of this Agreement.

1.119 “Regulatory Activities” means the Advanz Regulatory Activities or any regulatory

activities undertaken by Applied with respect to the Product, as applicable.

1.120 “Regulatory Approval”  means  any  approval,  with  respect  to  any  Country,  that  are
necessary  for  the  Commercialization  or  other  Exploitation  of  a  pharmaceutical  product  in  such
Country.    “Regulatory  Approval”  (a)  includes  all  approvals,  product  and  establishment  licenses,
registrations or authorizations of any federal, state or local authority, department, bureau or other
Governmental  Authority,  necessary  for  the  manufacture,  use,  storage,  importation,  export,
transport, sale, or placing on the market of a pharmaceutical product in a Country and (b) includes
any Marketing Authorization.

1.121 “Regulatory Authority” means, in respect of a particular Country, the Governmental

Authority having responsibility for granting Regulatory Approvals in such Country.

1.122 “Regulatory  Filing”  means  all  applications,  filings,  submissions,  approvals,
licenses,  registrations,  permits,  notifications  and  authorizations  (or  waivers)  with  respect  to  the
Commercialization  or  other  Exploitation  of  a  compound  or  pharmaceutical  product  made  to  or
received  from  any  Regulatory  Authority  in  the  Territory,  including  any  Marketing  Authorization
Applications and labels.

1.123 “Reimbursing Party” shall have the meaning assigned to it in Section 10.1(b).

1.124 “Requested Actions” shall have the meaning assigned to it in Section 8.14(c).

1.125 “Required Existing Studies” means all clinical studies for the Compound or Product
which are ongoing at the Effective Date including: (a) the long-term extension trial evaluating the
safety and pharmacokinetics of the Compound, in adult human subjects with Galactosemia being
conducted  by  Applied  and  referred  to  as  the  ACTION-Galactosemia  study  (the  “AT-007-1006
Study”),  (b)  the  pediatric  trial  evaluating  the  safety,  pharmacokinetics  and  reduction  in  the  toxic
biomarker, galactitol, as well as long-term clinical outcomes, such as speech, memory, cognition,
behavior, growth and development and motor skills of the Compound in children (ages 2-17) being
conducted by Applied and referred to as the ACTION-Galactosemia Kids study (the “AT-007-1002
Study”);  and  (c)  the  registrational  clinical  trial  evaluating  biomarker  efficacy,  clinical  outcomes
and safety in human subjects (ages 16 and older) with SORD treated with the Compound

18

vs. placebo being conducted by Applied and referred to as the INSPIRE study (the “AT-007-1005
Study”).

1.126 “Required Post-MA Studies”  means,  in  each  case,  with  respect  to  the  Product  for
use  in  the  Field  in  the  Territory,  any  (a)  pre-clinical  or  clinical  study  as  part  of  a  pediatric
investigational plan (a “PIP”) required by a Regulatory Authority within the Territory, either as a
condition  of  expanding  the  approved  Indication  under  a  Marketing  Authorization  for  another
subpopulation  or  as  an  associated  commitment  of  a  Marketing  Authorization;  (b)  confirmatory
studies  for  Galactosemia  for  adults  if  the  Product  is  being  Commercialized  under  conditional
Marketing Authorization; (c) post authorization efficacy study (“PAES”)  including  for  paediatric
use in respect of Galactosemia and in general in respect of SORD (but not including, for clarity,
any  studies  under  the  foregoing  subsection  (a));  or  (d)  other  pre-clinical  or  clinical  trial,  in  each
case of the foregoing (c) and (d), as required by any Regulatory Authority in any Country in the
Territory to maintain an existing Marketing Authorization for the Product for use in such Licensed
Indication.

1.127 “ROFO Negotiation Period” shall have the meaning assigned to it in Section 2.5(b).

1.128 “ROFO Product” shall have the meaning assigned to it in Section 2.5(a).

1.129 “ROFO Response Period” shall have the meaning assigned to it in Section 2.5(b).

1.130 “Royalties” shall have the meaning assigned to it in Section 9.3.

1.131 “Safety Stock” shall have the meaning assigned to it in Section 8.11(b).

1.132 “Secondary Source Site” shall have the meaning assigned to it in Section 8.12.

1.133 “Secondary  Packaging  and  Release”  means  finishing, 

labelling,  packaging
(including  design  of  artwork  and  any  translations)  and  quality  release  activities  to  the  extent
relating to the Product for use in the Field in the Territory.

1.134 “Secondary  Packaging  and  Release  Estimated  Cost”  shall  have  the  meaning

assigned to it in Section 8.6(d).

1.135 “Shelf Life Requirements” shall have the meaning assigned to it in Section 8.4(e).

1.136 “SORD” means sorbitol dehydrogenase deficiency.

1.137 “Step-In Notice” means notification by Advanz to Applied that it intends to exercise

its Step-In Rights in accordance with Section 8.14.

1.138 “Step-In  Rights”  means  the  right  of  Advanz  to  step-in  to  continue  any  activities
undertaken  or  required  to  be  undertaken  by  Applied  or  any  other  Person  on  Applied’s  behalf
relating to or associated with the Exploitation of the Product in accordance with this Agreement, as
and to the extent applicable, pursuant to Section 8.14.

18

1.139 “Sublicense”  means  the  grant  by  Advanz  of  a  sublicense  under  any  of  the  rights

licensed by Applied to Advanz pursuant to Section 2.1.

1.140 “Sublicensee”  means  a  Third  Party  to  whom  Advanz  has  granted  a  Sublicense  in

accordance with the terms and conditions set forth herein.

1.141 “Supply Shortage” shall have the meaning assigned to it in Section 8.13.

1.142 “Tax”  means  any  U.S.  and  non-U.S.  federal,  state,  local,  regional,  municipal,  or
other tax or taxation, levy, duty, charge, withholding, or other assessment of any kind (including
any  related  fine,  penalty,  addition  to  tax,  surcharge,  or  interest)  imposed  by,  or  payable  to,  a
Governmental Authority, including sales, use, excise, stamp, transfer, property, value added, goods
and services, withholding, and franchise taxes

1.143 “Technology”  means  all  technical,  scientific,  regulatory  and  other  information,
results,  knowledge,  techniques  and  data  (including  biological,  chemical,  pharmacological,
toxicological, pharmaceutical, physical and analytical, safety, quality control, and preclinical and
clinical data), in whatever form and whether or not confidential, patented or patentable, including
inventions,  invention  disclosures,  discoveries,  plans,  processes,  practices,  methods,  knowledge,
instructions, 
formulations,  compositions,
specifications and manufacturing data or descriptions.  “Technology” does not include Intellectual
Property claiming any of the foregoing.

skill,  experience, 

ideas,  concepts, 

formulae, 

1.144 “Term” shall have the meaning assigned to it in Section 15.1.

1.145 “Territory” means those Countries set forth on Exhibit D attached hereto.

1.146   “Third  Party”  means  any  Person  other  than  Advanz,  Applied,  or  any  of  their

respective Affiliates.

1.147 “Third Party Claim” shall have the meaning assigned to it in Section 17.4(a).

1.148 “Third Party License” means each license agreement between Applied and a Third
Party  pursuant  to  which  or  from  which  Applied  licenses  in  Applied  Patent  Rights  or  Applied
Technology as of the Effective Date, as notified to Advanz and set out in Exhibit E attached hereto.

1.149 “Third  Party  Product  Claim”  shall  have 

the  meaning  assigned 

to 

it 

in

Section 17.3(a).

1.150 “Total Supply Price” shall have the meaning assigned to it in Section 8.5(a)(ii).

1.151 “Trademarks”  means  trade  names,  brand  names,  trade  dress,  logos,  slogans,
trademarks and service marks and all other indicia of origin (whether registered or unregistered),
and  registrations,  applications  for  registration,  renewals  and  extensions  thereof,  together  with  all
translations,  adaptations,  combinations  and  derivations  thereof  and  all  goodwill  associated
therewith.

18

1.152 “United  Kingdom”  means  the  United  Kingdom  of  Great  Britain  and  Northern

Ireland.

1.153 “United  States”  or  “U.S.”  means  the  United  States  of  America,  including  its

territories and possessions.

1.154 “Valid Claim” means (a) a claim of an issued and unexpired Patent which has not
been  held  unpatentable,  invalid  or  unenforceable  in  a  final  decision  of  a  court  or  other
Governmental  Authority  of  competent  jurisdiction  from  which  no  appeal  may  be  or  has  been
taken,  and  which  has  not  been  admitted  to  be  invalid  or  unenforceable  through  reissue,  re-
examination or disclaimer; or (b) a claim of a Patent Application, which claim has been pending
less than [***] from the original priority date of such claim in a given jurisdiction, unless or until
such  claim  thereafter  issues  as  a  claim  of  an  issued  Patent  (from  and  after  which  time  the  same
shall be deemed a Valid Claim subject to clause (a) above).

1.155 “VAT” has the meaning assigned to it in Section 10.9(b).

1.156 Construction.    Except  where  expressly  stated  otherwise  in  this  Agreement,  the
following rules of interpretation apply to this Agreement: (a) “include,” “includes” and “including”
are  not  limiting  and  mean  include,  includes  and  including,  without  limitation;  (b)  definitions
contained  in  this  Agreement  are  applicable  to  the  singular  as  well  as  the  plural  forms  of  such
terms;  (c)  references  to  an  agreement,  statute  or  instrument  mean  such  agreement,  statute  or
instrument as from time to time amended, modified or supplemented; (d) references to a Person are
also to its permitted successors and assigns; (e) references to a “Section,” or “Exhibit” refer to a
Section of, or any Exhibit to, this Agreement unless otherwise indicated; (f) the word “will” shall
be  construed  to  have  the  same  meaning  and  effect  as  the  word  “shall”;  (g)  the  word  “any”  shall
mean “any and all” unless otherwise indicated by context; (h) the headings in this Agreement are
for  convenience  only  and  shall  not  affect  its  construction;  (i)  a  reference  to  a  particular  law  or
regulation is a reference to it as amended, extended or re-enacted from time to time and includes
any subordinate legislation made from time to time under that legislation or legislative provision;
(j)  except  as  otherwise  required  in  accordance  with  Section  3.1,  references  to  “writing”  or
“written” shall include emails; and (k) nothing in this Agreement shall in any way restrict or limit
any obligation of either Party to mitigate any loss or damage they may suffer in consequence of
any breach by the other Party of the terms of this Agreement, in consequence of any matter giving
rise to a claim against the other Party or otherwise in connection with this agreement.

SECTION 2. LICENSE

2.1

Licenses to Advanz.  Applied hereby grants to Advanz, and Advanz hereby accepts:

(a)

an exclusive (including with respect to Applied and its Affiliates, except as set forth
in  Section  2.2),  perpetual,  irrevocable  (except  where  Section  16.3(b)  applies),  sub-licensable  (in
accordance  with  Section  2.4),  non-transferable  (except  as  provided  in  Section  19.6),  royalty-
bearing license under the Applied Patent Rights and Applied Technology necessary or useful for,
and for purposes of, the following with respect to the Product in the Field in the Territory:

(i)

Secondary Packaging and Release in accordance with Section 8;

18

(ii)

Commercializing the Product; and

(iii)

the performance of Advanz’s obligations under Sections 5 and 6;

(b)

a sole (which for the purposes of this Section 2.2(b) shall be interpreted to include a
right  for  Applied  to  sub-license  its  rights  under  this  license  to  Applied’s  subcontractors  or
providers  for  purposes  of  Manufacture  or  Development),  perpetual,  irrevocable  (except  where
Section 16.3(b) applies), sub-licensable (in accordance with Section 2.4), non-transferable (except
as provided in Section 19.6), royalty-bearing license under the Applied Patent Rights and Applied
Technology necessary or useful for the performance of Advanz’s obligations under Sections 7.4(g)
and 11 and undertaking any activities required during Step-In Rights to:

(i)

(ii)

have Manufactured the Product for the Field in the Territory in accordance
with Section 8.14;

conduct  Development  of 
Section 4.3(c) or Section 8.14; and

the  Product 

to 

the  extent  permitted  by

(iii)

undertake infringement proceedings as set out in Sections 7.4 and 11; and

(c)

a non-exclusive, perpetual, irrevocable (except where Section 16.3(b) applies), sub-
licensable (in accordance with Section 2.4), non-transferable (except as provided in Section 19.6),
royalty-bearing  license  under  the  Applied  Patent  Rights  and  Applied  Technology  necessary  or
useful for permitting Advanz to exercise any of its other rights and perform any other obligations
set out in this Agreement.

2.2

Other License Provisions.

(a)

The license granted to Advanz pursuant to Section 2.1 shall be a sole license with
respect  to  Applied  to  the  extent  it  is  necessary  or  useful  for  Applied  to  perform  its  obligations
under this Agreement; for clarity, such sole license grant does not include the right for Applied or
any of its Affiliates to Commercialize the Product in the Field in the Territory.

(b)

The  Parties  expressly  acknowledge  and  agree  that  the  license  grants  in  favor  of
Advanz in Section 2.1 do not include and shall not be construed as limiting (i) Applied’s right to
Develop  or  Manufacture  the  Product  (or  the  Compound,  whether  or  not  for  use  in  the  Product),
(ii) Applied’s right to Develop, Manufacture or Commercialize the Product for use outside of the
Field  or  outside  of  the  Territory,  or  (iii)  any  of  Applied’s  other  rights  in  respect  of  the  Product
(including  its  rights  under  the  Applied  Patent  Rights)  outside  of  the  Field  or  outside  of  the
Territory.

(c)

In  addition  to  the  terms  and  conditions  of  this  Agreement,  Advanz  accepts  those
terms  and  conditions  of  the  Third  Party  Licenses  set  forth  on  Exhibit  H  as  they  relate  to  the
Product  and  the  rights  sublicensed  to  Advanz  under  this  Agreement.    For  purposes  of  clarity,
Advanz acknowledges that in the event Applied does not have exclusive rights to Applied Patent
Rights or Applied Technology licensed or obtained by Applied pursuant to a Third Party License,
Advanz’s  rights  to  such  Applied  Patent  Rights  or  Applied  Technology  under  the  sublicenses
granted under Section 2.1 will only be those rights granted by the Third Party to Applied.  Applied
shall comply

18

with its obligations under and enforce its rights under any Third Party License and shall ensure that
any amendments are not detrimental to Advanz.  If any Third Party License expires or terminates
for  any  reason,  Applied  shall  provide  all  reasonable  assistance  to  enable  Advanz  to  enter  into  a
direct contract with the Third Party licensor.

2.3

Non-Assertion of Rights.

(a)

During the Term, Advanz shall not, and shall cause its Affiliates not to, assert any
Patent Rights or Technology owned or Controlled by Advanz or its Affiliates against Applied, its
Affiliates or permitted sublicensees, distributors or end users in (i) exercising Applied’s rights and
performing  its  obligations  pursuant  to  this  Agreement  or  (ii)  using  or  Commercializing  the
Compound or Product outside the Territory or outside of the Field.

(b)

The  covenant  not  to  sue  in  Section  2.3(a)  shall  bind  any  acquiror  of  Advanz  and
inure to the benefit of the respective successors and permitted assigns of Applied, its Affiliates and
permitted sublicensees, distributors and end users.

2.4

(a)

Sublicensing and Subcontracting.

Advanz may grant Sublicenses to:

(i)

(ii)

(iii)

its contractors and other vendors for or in relation to Secondary Packaging
and Release activities;

its  Affiliates,  which  Sublicense  shall  automatically  terminate  when  such
Affiliate ceases to be an Affiliate of Advanz; and

reputable  Third  Parties,  with  respect  to  rights  to  Commercialize,  conduct
Regulatory  Activities  and  Pricing  and  Market  Access  Activities  in  relation
to the Product in the Territory;

provided  that  Advanz  must  obtain  the  express  written  consent  of  Applied  prior  to
entering  into  a  Sublicense  with  a  Third  Party  hereunder  (excluding  for  the
avoidance  of  doubt,  any  sublicenses  granted  pursuant 
the  foregoing
subsections (i) or (ii)), such consent not to be unreasonably withheld, conditioned or
delayed and to be provided within ten (10) days of Advanz’s request.  For clarity,
the Parties acknowledge and agree that Advanz’s contractors and logistics providers
are  not  Sublicensees  for  the  purpose  of  this  Agreement  to  the  extent  such
contractors and logistics providers do not obtain a sublicense under any Third Party
Licenses  and  Advanz  shall  be  entitled  to  engage  such  Third  Parties  without
Applied’s  consent  and  the  provisions  of  this  Section 2.4  other  than  Section  2.4(e)
shall not apply to such arrangements.

to 

(b)

Each  Sublicense  granted  by  Advanz  pursuant  to  Section  2.4(a),  other  than
Section 2.4(a)(i)  shall  be  subject  and  subordinate  to  the  terms  and  conditions  of  this  Agreement
shall contain the following provisions which, where the Sublicensee is an Affiliate of Advanz, may
be in the form of a side letter: (i) a requirement that such Sublicensee submit applicable sales or
other reports consistent with the requirements set forth in Section 10.1, (ii) a requirement to keep

18

books and records, and permit Advanz to audit (either directly or through an independent auditor)
such  books  and  records,  which  Advanz  shall  enforce  if  directed  and  reasonably  required  by
Applied  on  Applied’s  behalf,  (iii)  a  requirement  that  such  Sublicensee  comply  with  the
confidentiality  and  non-use  provisions  of  Section  12  with  respect  to  both  Parties’  Confidential
Information, (iv) a requirement to comply with all other applicable terms of this Agreement, (v) a
provision prohibiting such Sublicensee from further sublicensing the rights granted to it under the
Sublicense, (vi) with respect to any Sublicenses granting an Affiliate of Advanz set out in Exhibit J
(together with any additional Affiliates notified to Applied by Advanz from time to time and for
which Applied receives consent from [***], which, upon receipt of such consent, shall be deemed
to be included in Exhibit J) a sublicense under the [***], (A) a provision naming [***] as a third
party beneficiary to enable [***], to the extent permitted under Applicable Laws, solely to enforce
the  Applied  Patent  Rights  and/or  Applied  Technology  (in  each  case,  which  are  owned  by  [***])
and (B) and a provision stating that [***] has no liability to any such Sublicensee, Advanz shall
provide Applied with a copy of each such Sublicense (or any amendment to an existing agreement)
within ten (10) days after the execution of the applicable agreement (or amendment); provided that
Advanz may redact confidential information from such Sublicense that is not reasonably necessary
to  demonstrate  Advanz’s  compliance  with  the  obligations  set  forth  in  this  Agreement,  including
this Section 2.4.

(c)

Each Party may, subject to Section 12 and Sections 2.4(a)  and  (b),  subcontract  its
obligations under this Agreement to an Affiliate or Third Party as it would in the normal course of
its business without the prior written consent of the other Party.

(d)

Each Party shall ensure that each of its Affiliates, sublicensees and subcontractors
that perform activities on behalf of such Party under this Agreement accepts and complies with all
of  the  applicable  terms  and  conditions  of  this  Agreement  as  if  such  Affiliates  or  sublicensees  or
subcontractors were Parties to this Agreement.

(e)

Each  Party  shall  remain  fully  responsible  and  fully  liable  for  its  Affiliates’  and

sublicensees’ or subcontractors’ performance under this Agreement as if it were its own.

(f)

For clarity, the Parties acknowledge and agree that if this Agreement is terminated,
all  Sublicenses  shall  automatically  terminate  (other  than  those  Sublicenses  that  are  necessary  to
enable Advanz to exercise its Step-In Rights).

2.5

Right of First Offer for Additional Indications.  Applied hereby grants to Advanz a
right of first offer for the Commercialization in the Territory of any Additional Indication, upon the
terms and subject to the conditions set forth in this Section 2.5.

(a)

Upon  determining  that  it  will  seek  to  Commercialize  an  Additional  Indication  in
any  Country  in  the  Territory  (“ROFO  Product”)  through  a  license  or  collaboration  with  a  Third
Party,  Applied  shall  notify  Advanz  in  writing  thereof  (such  notice,  an  “Additional  Indication
Notice”).

(b)

Advanz  may,  within  [***]  of  its  receipt  of  the  Additional  Indication  Notice  (the
“ROFO  Response  Period”),  make  a  written  proposal  of  key  terms  to  Applied  for  the  exclusive
Commercialization of the ROFO Product for use in such Additional Indication and in which

18

Country in the Territory (a “Proposal”).   Applied  and  Advanz  shall  then  negotiate  exclusively  in
good  faith  for  a  period  not  to  exceed  [***]  from  the  date  Applied  received  the  Proposal,  in  an
effort to reach a definitive agreement for the exclusive Commercialization of the ROFO Product
for  use  in  such  Additional  Indication  and  in  which  Country  in  the  Territory  (the  “ROFO
Negotiation Period”).

(c)

In the event that (i) Advanz fails to, or notifies Applied in writing that it will not,
submit  a  Proposal  to  Applied  prior  to  the  expiration  of  the  ROFO  Response  Period,  (ii) Advanz
and  Applied  agree  to  discontinue  negotiations  during  the  ROFO  Negotiation  Period,  or
(iii)  Advanz  and  Applied  fail  to  enter  into  such  a  definitive  agreement  within  the  ROFO
Negotiation  Period,  Applied  shall  be  free  to  proceed  with  the  Commercialization  of  the  ROFO
Product  for  use  in  such  Additional  Indication  in  the  Countries  of  the  Territory  set  out  in  the
Proposal (including by entering into an agreement with one or more Third Parties therefor) subject
to Sections 2.5(d) and 2.5(e).

(d)

Applied  hereby  grants  Advanz  “most  favored  nation  status”  such  that  it  agrees  it
will  not  (i)  offer  nor  accept  terms  which  are  more  favorable  to  any  Third  Party  than  the  terms
which are contained in the Proposal or which have been negotiated with Advanz during the ROFO
Negotiation Period, nor (ii) enter into an agreement with a Third Party in respect of an Additional
Indication, in each case ((i) and (ii)) before the end of the ROFO Negotiation Period.

(e)

If Applied does offer or agree terms which are more favorable to any Third Party
than  the  terms  which  are  contained  in  the  Proposal  or  which  have  been  negotiated  with  Advanz
during the ROFO Negotiation Period or during the [***] period immediately following the expiry
of the ROFO Negotiation Period, it shall promptly provide notice thereof to Advanz.  Advanz shall
have  thirty  (30)  days  after  receipt  of  such  notice  to  reach  agreement  with  Applied  in  respect  of
such  terms  or  such  terms  as  may  be  agreed  between  the  Parties  and,  if  the  Parties  are  unable  to
reach  agreement  during  such  period,  Applied  shall  be  free  to  enter  an  arrangement  for  the
exclusive  Commercialization  of  the  ROFO  Product  for  use  in  such  Additional  Indication  with  a
Third Party.

(f)

If  Applied  Develops  the  ROFO  Product  for  use  in  an  Additional  Indication,  and
Advanz does not secure the rights to Commercialize the ROFO Product in the Territory for use in
such Additional Indication, then:

(i)

(ii)

(iii)

such  Additional  Indication  shall  not  be  included  in  the  ROFO  Product’s
then-existing Marketing Authorizations in the Territory;

the Licensed Trademarks  shall  not  be  applied  to  the  Additional  Indication;
and

within [***] after the end of the ROFO Negotiation Period or at such other
time  as  the  Parties  mutually  agree  in  writing,  the  Parties  shall  discuss  the
potential  adverse  impact  that  the  Commercialization  of  the  ROFO  Product
in the Territory for use in any such Additional Indication by a Third Party
may  have  on  the  Commercialization  of  the  ROFO  Product  by  Advanz  for
use  in  the  Field  in  the  Territory  provided  that  such  discussions  do  not  (A)
involve the sharing of commercially sensitive information about the

18

distribution strategy of Third Parties; nor (B) otherwise aim at coordinating
the  distribution  strategy  of  Advanz  and/or  any  Third  Parties.    Each  Party
agrees that Advanz’s commercial obligations under this Agreement will be
adjusted if Advanz can reasonably demonstrate that the Commercialization
of  the  ROFO  Product  in  the  Territory  for  use  in  any  such  Additional
Indication by a Third Party will compromise the potential for Advanz’s sale
of the Product.

2.6

Patent Challenges.

(a)

During  the  Term  of  this  Agreement,  Advanz  hereby  covenants  and  agrees  not  to,
and  shall  ensure  that  its  Affiliates  or  Sublicensees  do  not,  directly  or  indirectly,  commence  any
legal  proceeding,  or,  directly  or  indirectly,  provide  support  or  assistance  in  respect  of  any  legal
proceeding commenced by a Third Party, that challenges the validity, enforceability or ownership
of any Applied Patent Right to the extent such Applied Patent Right relates to the Compound or
Product  or  the  Development,  Manufacture,  Commercialization  or  other  Exploitation  of  the
Compound  or  Product  (a  “Patent Challenge”).    Without  limiting  the  generality  of  the  foregoing,
Advanz  specifically  agrees  that  filing  a  request  for  re-examination,  knowingly  copying  patent
claims so as to institute an interference, or filing an opposition with respect to any of the Applied
Patent Rights shall be deemed a Patent Challenge hereunder.

(b)

If Advanz or any of its Affiliates or Sublicensees directly or indirectly commences
(or provides any support or assistance in respect of) any Patent Challenge, Applied shall have the
right to immediately terminate this Agreement by written notice effective upon receipt by Advanz.
 The foregoing right of Applied to terminate this Agreement shall not apply to any such challenge
that arises out of or is in connection with any legal action commenced by Applied against Advanz,
in  which  Applied  asserts  any  Applied  Patent  Rights  or  other  Patent  Rights  against  Advanz,
whether arising out of or in connection with this Agreement or otherwise.

2.7

No Implied License; Negative Covenant.    Except  for  the  licenses  and  other  rights
expressly granted to Advanz herein, all right, title and interest in and to the Applied Patent Rights,
Applied Technology, and Applied Confidential Information (and all modifications, derivatives and
improvements  thereof),  and  any  and  all  Intellectual  Property  and  other  rights  of  Applied  or  its
Affiliates  not  expressly  granted  to  Advanz  hereunder  (including,  for  clarity,  all  of  the  foregoing
with  respect  to  any  Out-of-Scope  Products),  shall  remain  solely  with  Applied,  its  Affiliate  or  its
Third  Party  licensors,  as  applicable,  and  Advanz  hereby  covenants  not  to  practice  any  such
Intellectual  Property  outside  the  scope  of  the  licenses  granted  hereunder.    Except  as  expressly
provided in this Agreement, neither Party will be deemed by this Agreement to have been granted
any  license  or  other  rights  to  the  other  Party’s  Intellectual  Property,  either  expressly  or  by
implication,  estoppel  or  otherwise.    Notwithstanding  anything  to  the  contrary  in  this  Agreement,
the  Parties  acknowledge  and  agree  that  the  Development  and  Commercialization  of  any  Out-of-
Scope Products (including any Additional Indications) shall not be within the scope of the licenses
granted to Advanz pursuant to Section 2 hereunder (except as expressly provided in Section 2.5).

18

SECTION 3. ALLIANCE MANAGERS

to 

3.1

the 

facilitate 

In  order 

Alliance  Managers. 

information-sharing  and
communication provided for in this Agreement, upon or promptly following the execution of this
Agreement, the Parties shall each designate an employee of appropriate experience and authority
(an  “Alliance  Manager”)  to  act  as  the  first  and  primary  point-of-contact  for  ordinary  course
communications  regarding  the  matters  contemplated  by  this  Agreement.    Except  with  respect  to
Disputes,  termination  or  assignment  notices,  consents  or  other  matters  of  legal  import  (in  which
cases formal notice shall be delivered in accordance with Section 19.8), or with respect to Pricing
and Market Access Activities (in which case notice shall be delivered to the Pricing and Market
Access Committee), where this Agreement provides for notice or other written communication to a
Party,  such  notice  or  information  shall  be  provided  to  the  applicable  Alliance  Manager  or  its
designee and may be provided by email.  A Party may change its Alliance Manager at any time
upon reasonable prior notice in writing to the other Party.

SECTION 4. DEVELOPMENT

4.1

Development  Responsibilities.    Subject  to  this  Section  4,  as  between  the  Parties,
Applied  shall  have  sole  authority  for,  and  be  solely  responsible  for,  the  Development  of  the
Product  in  the  Field  including  any  and  all  clinical  studies  with  respect  to  the  Product,  except  as
otherwise expressly  provided  in  this Section 4.   Applied  shall  use  best  endeavors  to  conduct  the
Development necessary to obtain Marketing Authorization approval for the Product in the Field in
the  Territory  and  shall  use  Commercially  Reasonable  Efforts  to  comply  with  any  timeframe  or
other requirements therefor specified by the Regulatory Authorities and shall provide Advanz with
regular updates on any pre-clinical studies or clinical trials conducted as part of the Development
of  the  Product  in  the  Field  in  the  Territory,  whether  before  or  after  grant  of  any  Marketing
Authorization.  Applied shall use Commercially Reasonable Efforts to assist Advanz in filing and
obtaining  Marketing  Authorizations  for  the  Product  for  use  in  the  Field  in  all  Countries  in  the
Territory  in  accordance  with  Section  5;  provided  that,  Advanz  acknowledges  and  agrees  that,
notwithstanding  anything  in  this  Agreement  to  the  contrary,  Applied  makes  no  guarantees  or
assurances regarding any such Marketing Authorization or the Commercialization of the Product.

4.2

Changes to Specifications and Other Modifications to the Product.  In the event of
any changes required by Applicable Laws, the Parties shall use Commercially Reasonable Efforts
to comply with such changes (for clarity, without limitation to Section 8.8 hereof).  In the event of
other  changes  or  proposed  improvements  regarding  the  Product  relating  to  the  Field  in  the
Territory,  the  Parties  shall  discuss  in  good  faith  any  such  changes  and  improvements  and  the
allocation of requirements and responsibilities on each Party with respect thereto.  Required Post-
MA  Studies  or  Other  Post-Approval  Studies  in  connection  with  any  such  changes  and
improvements shall be subject to Section 4.3 hereof.

4.3

(a)

Development Costs.

Required Existing Studies.  Applied shall be responsible for [***] of all Costs and

Expenses incurred in conducting the Required Existing Studies.

18

 
(b)

Required  Post-MA  Studies.    The  Parties  will  share  the  amount  of  Costs  and

Expenses incurred in conducting the Required Post-MA Studies as follows:

(i)

(ii)

If data from the Required Post-MA Study (A) is to be used or referred to as
part of any regulatory or market access requirement or commitment outside
the  Territory  as  well  as  within  the  Territory,  or  (B)  would  benefit
Commercialization  of  the  Product  outside  the  Territory  as  well  within  the
Territory,  then  Applied  shall  bear  [***]  of  the  Costs  and  Expenses,  and
Advanz shall bear [***] of the Costs and Expenses; and

If data from the Required Post-MA Study is to be used or referred to as part
of any regulatory or market access requirement or commitment only within
the  Territory,  Applied  shall  bear  [***]  of  the  Costs  and  Expenses,  and
Advanz  shall  bear  [***]  of  the  Costs  and  Expenses  except  that  [***]  the
Costs and Expenses relating to any Required Post-MA Study set out in limb
(C) of the Required Post-MA Study definition.

(c)

Advanz  Development.    For  clarity,  except  where  Advanz  exercises  its  Step-In
Rights  under  Sections  8.14  or  16.3(a)  as  applicable  and  with  reference  to  Section  18.2,  Advanz
shall  not  have  any  rights  to  Develop  the  Product;  provided  that,  solely  if  Applied  provides  its
express written consent (not to be unreasonably withheld), Advanz will have the right to conduct
Other  Post-Approval  Studies  for  use  in  the  Field  in  the  Territory.    In  the  event  that  Applied
consents to any such Other Post-Approval Study, (i)  [***], and (ii) Advanz will grant to Applied a
perpetual, irrevocable (except where Section 16.3(b) applies) license to Exploit any data or other
Intellectual Property developed in the conduct thereof, to the extent related to the Product, for use
inside and outside the Field in Applied’s business, on commercially reasonable terms.

(d)

Other Post-Approval Studies outside the Territory.  Notwithstanding anything to the
contrary,  nothing  herein  shall  prevent  Applied  from  conducting,  at  its  sole  discretion,  any
Development with respect to the Product, whether for use inside or outside the Field, including any
Other Post-Approval Studies.  In the event that Applied conducts any such studies related to the
Product in the Field that include the Territory, Applied shall: (i) notify Advanz in advance thereof
and reasonably consult with Advanz in connection therewith; (ii) [***]; and (iii) grant to Advanz a
perpetual, irrevocable license (except where Section 16.3(b) applies) to Exploit any data or other
Intellectual Property developed in the conduct thereof, to the extent related to the Product, for use
in  Advanz’s  business  relating  to  the  Product  in  the  Territory  and  in  the  Field  on  commercially
reasonable terms.

SECTION 5. REGULATORY AFFAIRS

5.1

(a)

Responsibility.

Advanz  shall  be  responsible  for  conducting  and  shall  conduct  the  Advanz

Regulatory Activities, in accordance with Applicable Laws and the terms and conditions hereof.

(b)

Regardless  of  which  Parties’  Regulatory  Activities  are  involved,  all  Regulatory
Filings  with  Regulatory  Authorities  in  the  Territory  pertaining  to  the  Product  within  the  Field,
including any Marketing Authorization Applications and any resulting Marketing Authorizations,

18

shall  be  submitted  by,  made  and  held  in  the  name  of  Advanz,  an  Advanz-specified  Affiliate  or
designee  company.    Applied  shall  prepare  the  Marketing  Authorization  Applications  for  the
Product  in  the  Field  in  the  Territory,  including  completing  any  forms  and  compiling  the  Dossier
and  other  information  required  to  submit  any  such  Marketing  Authorization  Application  and
Advanz shall submit such Marketing Authorization Application.  Applied shall provide a copy of
the Dossier to Advanz as soon as possible and no later than [***] before the planned submission
date to the applicable Regulatory Authority to enable Advanz to provide comments and the Parties
to reach an agreement on the content of the Dossier.  Obtaining and maintaining such Marketing
Authorizations  shall  be  a  collaborative  effort  between  the  Parties.    For  the  avoidance  of  doubt,
Applied  shall  be  responsible  for  [***]  the  preparation  and  provision  of  all  data  and  information
which  is  required  to  be  included  in  or  with  the  Dossier  to  obtain  the  applicable  Marketing
Authorization  (whether  conditional  or  otherwise)  for  the  Product  in  the  Field  in  the  Territory
(including  a  full  environmental  risk  assessment  report,  GCP  inspections,  ERA,  GLP  statements,
any  phase  3  studies  for  pediatric  Galactosemia  (excluding,  for  clarity,  any  PIP)  or  in  general  in
respect  of  SORD  and  other  non-clinical  studies)  [***].    Prior  to  submission  of  any  Marketing
Authorization Application or amendment thereto by Advanz, the Parties will collaborate to ensure
mutual agreement on the final Marketing Authorization Application (or any amendment thereto) to
be  submitted;  provided  that  Advanz  may  not  finally  submit  the  same  without  Applied’s  prior
written  consent  (not  to  be  unreasonably  withheld,  conditioned  or  delayed).    With  respect  to  any
other  Regulatory  Filings  for  the  Product  in  the  Field  in  the  Territory,  Advanz  shall  prepare  and
submit  such  Regulatory  Filings  at  its  cost  and  expense  (subject  to  Section  5.2(b));  provided  that
Applied  shall  reasonably  cooperate  with  respect  thereto  and  shall  provide  necessary  data  and
information in its possession at its cost and expense.

(c)

No  later  than  [***]  before  the  planned  submission  date  of  the  first  Marketing
Authorization  Application,  the  Parties  shall  enter  into  a  Quality  Agreement  including  Applied’s
obligations to carry out ongoing stability studies and annual quality review (PQR) in relation to the
Product at its cost and expense.

5.2

Communications with Regulatory Authorities.

(a)

Advanz  shall  provide  Applied  with  notice  of  all  meetings  and  discussions
(including advisory committee meetings or any other meeting of experts convened by a Regulatory
Authority)  scheduled  with  a  Regulatory  Authority  concerning  any  Advanz  Regulatory  Activities
promptly after the scheduling of such meeting, conference, or discussion (and in any event, within
[***] or such shorter time as reasonably necessary to enable Applied’s participation in accordance
with this Section 5.2(a)).  Applied shall be entitled to have one or more representatives present at
all  such  meetings  to  the  extent  permissible  under  Applicable  Laws  and  reasonably  practicable
under  the  circumstances.   The  Parties  shall  use  all  reasonable  efforts  to  agree  in  advance  on  the
scheduling  of  such  meetings,  conferences  and  discussions  and  shall  discuss  in  good  faith  the
objectives  to  be  accomplished  at  such  meetings,  conferences  and  discussions  and  the  agenda
therefor, if any.

(b)

Advanz  shall  provide  Applied  with  copies  of  all  material  submissions  to  any
Regulatory Authority relating to the Advanz Regulatory Activities.  Such copies shall be provided
sufficiently in advance of such planned submission to the applicable Regulatory Authority in order
to allow Applied to provide comments regarding such submission.  Advanz shall consider and

18

reflect Applied’s comments in good faith with respect to such submission, and, to the extent such
submission  constitutes  a  Regulatory  Filing  hereunder,  may  not  finally  submit  the  same  without
Applied’s  prior  written  consent  not  to  be  unreasonably  delayed,  withheld  or  conditioned,  such
consent to be provided or rejected within [***] of Advanz’s request.  If Applied does not respond
within [***], it shall be deemed to have given its consent.

(c)

Without limitation to the Parties’ cooperation under Sections 5.3 and 5.4, each Party
shall provide to the other Party, as soon as reasonably practicable but in no event more than three
(3)  Business  Days  (or  twenty-four  (24)  hours,  to  the  extent  the  same  concerns  any  safety  issue)
after its receipt, copies of any material documents or other material correspondence received from
a Regulatory Authority pertaining to the Compound or the Product.

5.3

Cooperation; Regulatory Information.    Subject  to  the  remainder  of  this  Section  5,
the  Quality  Agreement  and  the  Pharmacovigilance  Agreement,  each  Party  agrees  to  provide  the
other with all reasonable information and assistance and take actions reasonably requested by the
other Party to undertake its respective Regulatory Activities or that are necessary or desirable to
enable the other Party to comply with Applicable Laws with respect to the Product (including, for
clarity,  to  enable  Advanz  to  apply  for,  update  or  maintain  the  Marketing  Authorization  in  the
Territory or comply with regulatory requirements with respect to the Product outside the Territory).
 For the avoidance of doubt, with the exception of clinical studies (which are excluded from this
Section  5.3  but  with  respect  to  which  certain  data  may  be  provided  pursuant  to  Section  4.3  or
Section 5.1), the foregoing shall include any and all such data and other information generated by
each Party in the course of its performance under this Agreement, the Quality Agreement, or the
Pharmacovigilance  Agreement,  which  information:  (a)  Applied  shall  have  the  rights  to  use  in
respect  of  its  business  regarding  the  Product  generally  (whether  inside  or  outside  the  Field  or
Territory);  and  (b)  Advanz  shall  have  the  rights  to  use  in  respect  of  its  business  regarding  the
Product in the Field in the Territory.  For clarity and subject to the other terms of the Agreement
including Section 4.3(b), to the extent that either Party provides reasonably requested assistance to
the other Party in compliance with this Section 5.3, the requesting Party shall promptly reimburse
such Party for any reasonable Costs and Expenses incurred in respect thereof.

5.4

Pharmacovigilance.  Subject to the remainder of this Section 5.4, Advanz shall have
the  primary  responsibility  for  conducting  all  pharmacovigilance  activities  with  respect  to  the
Product in the Field in the Territory, including conducting PV and Risk Management Studies, post-
marketing surveillance, addressing product complaints, and investigating and reporting safety data
and adverse events, as required under Applicable Laws, at its cost and expense, unless otherwise
agreed  in  the  written  pharmacovigilance  agreement  to  be  entered  into  between  the  Parties  (the
“Pharmacovigilance Agreement”).  Advanz shall keep Applied duly informed of any matters which
Advanz reasonably believes may present a material risk to the Product (including outside the Field
or the Territory) or should otherwise be recorded by Applied on the global safety database for the
Product  held  by  Applied.  After  the  Effective  Date,  and  in  no  case  later  than  Advanz  obtaining
Marketing Authorization for the Product in the Field in the Territory, the safety units of each of the
Parties  shall  meet  and  agree  upon  a  Pharmacovigilance  Agreement  that  shall  set  forth  in  greater
detail  such  pharmacovigilance 
the
Pharmacovigilance  Agreement  shall  also  set  forth  a  process  for  exchanging  all  relevant
information and data, including adverse event reports and other safety information relating to the
Product as reasonably necessary to enable each Party (and, in the case of Applied, its licensees in

responsibilities. 

  Without 

foregoing, 

limiting 

the 

18

any  Country  outside  the  Territory)  to  comply  with  Applicable  Laws  and  requirements  of
Regulatory Authorities in relation to the Product.  Notwithstanding anything to the contrary herein,
the  Pharmacovigilance  Agreement  shall  provide  that  Applied  shall  own  and  maintain  the  global
safety  database  for  the  Product.    Except  as  may  be  otherwise  mutually  agreed  in  the
Pharmacovigilance  Agreement,  each  Party  will  bear  its  own  Costs  and  Expenses  in  connection
with its activities thereunder.

5.5

Recalls or Other Corrective Action.

(a)

Advanz  shall  promptly  notify  Applied  and  provide  all  reasonably  pertinent
information regarding any potential recall or market withdrawal or other material corrective action
related  to  the  Product  in  the  Field  in  the  Territory  proposed  to  be  undertaken  by  Advanz  (an
“Advanz  Recall”).    Applied  shall  promptly  notify  Advanz  and  provide  all  reasonably  pertinent
information regarding any potential recall or market withdrawal or other material corrective action
related  to  the  Product  or  Compound  proposed  to  be  undertaken  by  Applied  or  its  Sublicensees
outside of the Territory or the Field (an “Applied Recall”).

(b)

To  the  extent  reasonably  practicable,  the  Parties  shall  consult  regarding  the
diagnosis  and  assessment  of  the  circumstances  leading  to  any  Product  Recall  relating  to
Manufacturing,  and  each  Party  shall  consider  in  good  faith  all  information  and  considerations
presented by the other Party The Parties recognize that in the case of an urgent safety issue, such
advance  consultation  may  not  be  possible.    Nevertheless,  each  Party  shall  reasonably  cooperate
with the other Party to manage any messaging or communication with Regulatory Authorities in
connection with any Product Recall (whether before or after such Product Recall).

(c)

The final decision to initiate any Advanz Recall shall be made by Advanz, at its sole
discretion,  and  the  final  decision  to  initiate  any  Applied  Recall  shall  be  made  by  Applied,  at  its
sole discretion.

(d)

Advanz  shall  be  responsible  for  executing  any  Advanz  Recall  at  its  cost  and
expense,  save  that  to  the  extent  that  any  Advanz  Recall  is  due  to  the  breach  of  this  Agreement,
gross  negligence,  or  willful  acts  or  omissions  of  Applied,  Applied  shall,  at  its  own  cost,  be
responsible for supplying replacement Bulk Product and shall promptly reimburse Advanz for all
fines or penalties and all reasonable Costs and Expenses incurred by Advanz in connection with
the Advanz Recall.

5.6

Early  Access  Programs.    Advanz  shall  have  the  right  to  decide  whether  to
participate  in  any  Early  Access  Programs  applicable  to  the  Product  in  the  Field  in  the  Territory
[***].

5.7

Safety and Regulatory Inspections.  Advanz and Applied shall promptly (but in any
event no later than five (5) Business Days after receiving the applicable notice) notify each other of
any audit or inspection of Advanz or Applied or their Affiliates, Sublicensees or subcontractors by
any  Regulatory  Authority  relating  specifically  to  the  Product  and  shall  share  with  each  other  all
relevant  information  in  their  control,  to  the  extent  this  relates  to  the  Product.    Subject  to  any
required approvals of the Regulatory Authority and of any relevant Third Party, Applied shall have

18

the  right,  but  not  the  obligation,  to  be  present  at  and  participate  in  any  such  audit  or  inspection
relating specifically to the Product, at its sole cost and expense.

SECTION 6. PRICING AND MARKET ACCESS

6.1

Pricing and Market Access Committee.

(a)

As  soon  as  reasonably  practicable  following  the  Effective  Date  (and,  in  any  case
within forty-five (45) days thereof), the Parties shall form a committee (the “Pricing and Market
Access Committee”  or  the  “PMAC”)  to  exchange  information  and  facilitate  communication  and
oversight  with  respect  to  Pricing  and  Market  Access  Activities  in  the  Field  in  the  Territory
hereunder.

(b)

The PMAC shall be composed of [***] members (the “PMAC Members”).    Each
Party shall have the right to appoint [***] of its employees to serve as PMAC Members, each of
whom shall have appropriate knowledge with respect to pricing, reimbursement, and other market
access affairs in the Territory.  Upon written notice to the other Party, each Party shall be entitled to
appoint  an  appropriately  qualified  substitute  PMAC  Member.    The  PMAC  shall  meet  (either  in
person or via telephone or video conference) at mutually agreeable dates; provided that the PMAC
Members  shall  meet  as  frequently  as  reasonably  necessary  to  achieve  the  goals  set  forth  in  this
Section 6.  Upon invitation of either Party, other representatives of the Parties shall be allowed to
attend  such  meetings  (provided  such  representatives  are  subject  to  reasonable  confidentiality
restrictions).    Each  Party  shall  bear  all  expenses  of  its  respective  PMAC  Members  and
representatives with respect to their participation in the PMAC.

6.2 Market Access Activities.

(a)

Advanz  shall  have  the  sole  responsibility  for  undertaking  all  Pricing  and  Market
Access Activities in Advanz’s name in the Territory including obtaining and maintaining any and
all applicable Price Approvals, with respect to the Product in the Field in the Territory, subject to
this Section 6.  Advanz shall reasonably consult and cooperate with Applied through the PMAC in
undertaking  all  such  activities.    Without  limiting  the  foregoing,  Advanz  shall  use  Commercially
Reasonable Efforts to obtain the best possible reimbursement price for the Product in the Field in
each Country in the Territory in which such pricing and reimbursement is applicable.

(b)

Advanz will keep Applied reasonably informed through the PMAC (and at any time
upon Applied’s request) regarding the status and details of Pricing and Market Access Activities in
each applicable Country in the Territory.  In the event that Advanz reasonably requests any data or
information from Applied that is reasonably necessary or useful to conduct any Pricing and Market
Access Activities, Applied shall provide such data or information to Advanz in a prompt manner in
respect  of  the  nature  and  complexity  of  such  request.    Advanz  may  provide  any  such  data  or
information directly to a Regulatory Authority or applicable Third Party at its sole discretion.

(c)

Advanz shall consider in good faith all input provided by Applied in the PMAC or
otherwise from time to time with respect to such Pricing and Market Access Activities (including
strategy and approach).  For the avoidance of doubt, Advanz will be free to determine the resale
price of the Product in the Territory.

18

SECTION 7. COMMERCIALIZATION

7.1

Diligence.   Advanz  shall  have  the  exclusive  right  to  Commercialize,  and  shall  be
responsible  for  paying  all  Costs  and  Expenses  associated  with  the  Commercialization  of,  the
Product  in  the  Field  in  the  Territory.    Without  limiting  the  foregoing,  during  the  Initial  Royalty
Term,  Advanz  shall  use  Commercially  Reasonable  Efforts  to  Launch  and  Commercialize  the
Product in all of the Major Markets for which Marketing Authorization for a Licensed Indication is
obtained (which in Germany shall be within [***] after the grant of any Marketing Authorization
for  the  Product  for  such  Licensed  Indication  by  EMA  and  in  France  shall  be  within  [***]  from
securing Price Approval and/or Third Party reimbursement approval where applicable); provided
that:

(a)

Applied has delivered Product in accordance with the quantities and delivery date
set  out  in  the  Purchase  Order  in  compliance  with  cGMP,  the  specifications,  the  applicable
Marketing Authorization, Applicable Laws and the Quality Agreement, and

(b)

the Launch in the applicable Country will not reasonably result in the infringement

of Intellectual Property owned by a Third Party.

7.2

Commercialization  Plan.    Within  [***]  after  the  Effective  Date,  Advanz  shall
prepare  and  provide  to  Applied  a  Commercialization  plan  for  the  Product  in  the  Field  in  the
Territory (the “Initial Commercialization Plan”).  Advanz shall update such plan (any such updated
plan,  the  “Commercialization  Plan”)  at  least  once  per  Calendar  Year.    Each  such  subsequent
Commercialization  Plan  shall  be  submitted  to  Applied  for  review  and  discussion  no  later  than
[***] prior to the beginning of the immediately succeeding Calendar Year.  Applied may propose
to  Advanz  revisions  to  any  such  subsequent  Commercialization  Plan,  and  any  proposed  material
updates  or  amendments 
Initial  Commercialization  Plan  and  any  subsequent
Commercialization  Plan,  that  Applied  reasonably  believes  are  appropriate,  and  Advanz  shall
consider any such proposed revisions in good faith.

the 

to 

7.3

Product Diversion.

(a)

Advanz hereby agrees to refrain from selling the Product to any Person if Advanz
has knowledge or reason to believe that such Product is intended for transshipment or delivery by
such  Person  outside  the  Territory  or  for  use  outside  of  the  Field  (whether  within  or  outside  the
Territory).    If  Advanz  determines  that  any  such  diversion  is  occurring,  then  Advanz  will  use
Commercially Reasonable Efforts to promptly cease delivery of the Product to the applicable Third
Parties and revenue generated from such sales, will be paid by Advanz to Applied.

(b)

Applied hereby agrees to refrain from selling the Product to any Person if Applied
has knowledge or reason to believe that such Product is intended for transshipment or delivery by
such Person to the Territory for use in the Field.  If Applied determines that any such diversion is
occurring, then Applied will use Commercially Reasonable Efforts to promptly cease delivery of
the Product to the applicable Third Parties and revenue generated from such sales, will be paid by
Applied to Advanz.

7.4

Trademarks.

18

(a)

License  to  Advanz.    Applied  hereby  grants  to  Advanz  a,  perpetual,  irrevocable
(except  where  Section  16.3(b)  applies),  sub-licensable  (in  accordance  with  Section  2.4),  non-
transferable  (except  as  provided  in  Section  19.6),  royalty-bearing  license  to  use  the  Licensed
Trademarks in the Territory:

(i)

(ii)

on  an  exclusive  basis  with  respect  to  Secondary  Packaging  and  Release  in
accordance with Section 8, Commercialization of the Product for use in the
Field  in  the  Territory  and  the  performance  of  Advanz’s  obligations  under
Sections 5 and 6 for purposes of performing such obligations;

on  a  sole  basis  (which  for  the  purposes  of  this  Section  7.4(a)(ii)  shall  be
interpreted to include a right for Applied to sub-license its rights under this
license to Applied’s Bulk Product contract manufacturer) with respect to the
performance  of  Advanz’s  obligations  under  Sections  7.4(g)  and  11  and
undertaking any activities required during Step-In to have Manufactured the
Product  for  the  Field  in  the  Territory  in  accordance  with  Section  8.14,  to
conduct  Development  of 
the  extent  permitted  by
Section  4.3(c)  and  to  undertake  infringement  proceedings  in  accordance
with Section 7.4 or 11; and

the  Product 

to 

(iii)

on a non-exclusive basis with respect to permitting Advanz to exercise any
of  its  other  rights  and  perform  any  other  obligations  set  out  in  this
Agreement,

each in accordance with this Agreement.

Advanz  shall  cooperate  with  Applied  in  respect  of  recording  (and  take  any  actions  reasonably
requested  by  Applied  to  record)  this  trademark  license  (including,  as  may  be  appropriate,
executing  a  short  form  thereof  for  purposes  of  recordation)  with  the  appropriate  Governmental
Authorities throughout the Territory to the extent reasonably required or requested by Applied (and
Applied shall be responsible for paying all Costs and Expenses associated with such recordation).
 Where applicable under Section 16.3, Advanz shall cooperate with Applied to effect a cancellation
or  termination  of  any  such  recordation  with  the  appropriate  Governmental  Authorities  in  the
Territory, and, if requested by Applied, Advanz agrees to grant to Applied an irrevocable power of
attorney  coupled  with  an  interest  to  effect  such  cancellation  within  twenty  (20)  days  after  the
termination of this Agreement.

(b)

Product Trademarks.  Advanz may choose to use the Licensed Trademarks or any
other product Trademarks to Commercialize the Product in the Field in the Territory; provided that
(i)  use  of  such  other  product  Trademarks  shall  be  subject  to  Applied’s  approval  in  advance  in
writing,  which  approval  shall  not  be  unreasonably  withheld,  conditioned  or  delayed,  and
(ii)  Applied  shall  own  all  such  other  product  Trademarks,  which  shall  be  deemed  Licensed
Trademarks hereunder.  For the avoidance of doubt, Applied shall have no right, title or interest in
any Trademark using or incorporating Advanz’s corporate name.  Advanz shall use the Licensed
Trademarks (including such other product Trademarks referred to in the foregoing sentence) and
no  other  product  Trademarks  to  Commercialize  the  Product  in  the  Field  in  the  Territory.    For
clarity, nothing in this Section 7.4(b) shall restrict Advanz from using the Advanz corporate name

18

on  package  inserts,  packaging  or  trade  packaging  associated  with  the  Product  in  the  Territory  in
accordance with Applicable Laws.

(c)

Ownership  of  Licensed  Trademarks. 

  Advanz  acknowledges  the  exclusive
ownership  by  Applied  of  the  Licensed  Trademarks  (and  any  Trademark  containing,  comprising,
derivative  of  or  confusingly  similar  to  the  Licensed  Trademarks)  including  any  product
Trademarks selected by Advanz pursuant to Section 7.4(b).  Advanz shall not (and shall ensure that
its  Affiliates  do  not),  directly  or  indirectly,  during  the  Term  of  thereafter,  register  or  attempt  to
register (or obtain any other ownership right in) any such Trademarks in its own name or challenge
or assist others to challenge any such Trademarks (or the validity or enforceability of, or Applied’s
rights in, the same).  This Agreement does not confer on Advanz any goodwill associated with the
Licensed Trademarks or generated from the use thereof (all of which shall inure to Applied).

(d)

Use  of  Licensed  Trademarks.   Advanz  shall  comply  with  any  applicable  branding
guidelines  applicable  across  its  organization  in  respect  of  the  Licensed  Trademarks  that  are
provided to Advanz by Applied from time to time.  Advanz shall submit to Applied samples of all
the uses of the Licensed Trademarks (including on any packaging or labeling of Products bearing
the Licensed Trademarks), for Applied’s approval prior to the first use thereof.  Applied will have
the  right  to  inspect,  upon  reasonable  notice  and  during  normal  business  hours,  Advanz’s  and  its
Affiliates’  and  Sublicensees’  premises,  records,  operations,  materials  and  samples  in  connection
with the use of the Licensed Trademarks to ensure compliance with this Agreement.

(e)

Quality Control.

(i)

(ii)

The quality of the Product (including all associated packaging and labeling
bearing  the  Licensed  Trademarks)  sold  or  distributed  by  Advanz  in  the
Territory under or in connection with the Licensed Trademarks and the use
by Advanz of the Licensed Trademarks (including in marketing, advertising
and  promotional  materials)  shall,  subject  to  Applied’s  compliance  with
Section 8.2, comply with cGMP and cGDP.

Advanz shall (A) comply with all Applicable Laws pertaining to the proper
use  and  designation  of  the  Licensed  Trademarks,  (B)  use  the  Licensed
Trademarks  only  in  the  form  and  manner  and  with  appropriate  legends  as
prescribed  or  otherwise  approved  from  time  to  time  during  the  Term  by
Applied, (C) display the proper form of trademark notice associated with the
Licensed  Trademarks,  (D)  not  use  any  Licensed  Trademark  as  a  corporate
name, business name, or trade name, (E) not use any Licensed Trademark in
a  manner  that  would  reasonably  be  expected  to  materially  impair  the
validity, reputation, or distinctiveness of any Licensed Trademark or create a
combination  mark  with  any  other  Trademarks,  (F)  use  any  Licensed
Trademark at a level of quality set out in Section 7.4(e)(i), and (G) not use
any Licensed Trademark in a manner that would reasonably be expected to
materially  tarnish,  impair  or  otherwise  adversely  affect  the  reputation  of
Advanz, Applied or any of their respective Affiliates.

18

(f)

Prosecution and Maintenance of Trademarks.  Applied shall prosecute and maintain
(and defend against oppositions and challenges to) the Licensed Trademarks in the Territory in the
name of Applied, at its sole cost and expense.  Applied shall keep Advanz reasonably informed of
any  actions  taken  in  respect  of  the  prosecution  and  maintenance  of  (and  defense  against
oppositions  and  challenges  to)  Licensed  Trademarks  in  the  Territory  (and  shall  provide  Advanz
with  updates  regarding  the  status  of  any  Licensed  Trademarks  in  the  Territory  upon  Advanz’s
request).

(g)

Enforcement of Trademarks.  Each Party will promptly notify the other in the event
of any actual, potential or suspected infringement of any Licensed Trademark by any Third Party
in the Territory.

(i)

Applied shall at its cost:

(A)

(B)

institute  litigation  or  take  other  remedial  measures  in  connection
with  Third  Party  infringement  or  other  violation  of  Licensed
Trademarks in the Major Markets; and

use  Commercially  Reasonable  Efforts  to  institute  litigation  or  take
other remedial measures in connection with Third Party infringement
or  other  violation  of  Licensed  Trademarks  in  all  other  Countries  in
the Territory.

If  Applied  elects  not  to  initiate  litigation  or  take  other  remedial  measures
against a Third Party who is alleged to be infringing or otherwise violating a
Licensed Trademark in a Country other than a Major Market in the Territory
in  the  Field  within  [***]  of  Advanz’s  request  that  Applied  do  the  same
(provided that, if Applied intends to undertake such defense, Applied shall
notify Advanz that it intends to do so with [***] of Advanz’s request), then
it shall consult with Advanz to discuss the repercussions of such a decision
on  Advanz’s  other  markets  in  the  Territory.    If  Advanz,  at  its  sole  but
reasonable  discretion,  considers  that  a  failure  to  institute  litigation  or  take
other remedial measures will have an adverse impact on Advanz’s business
relating to the Products, then Advanz shall have the right to initiate litigation
or  take  other  remedial  measures  at  its  own  cost.   Applied  shall  provide  to
Advanz all reasonable assistance in connection with such litigation or other
remedial  measures.    Advanz  shall  be  entitled  to  retain  any  recoveries
obtained resulting from any such litigation or other measures.

Applied shall have the sole right, but not the obligation, to institute litigation
or take other remedial measures in connection with Third Party infringement
or other violation of Licensed Trademarks outside the Territory or outside of
the Field.

Any Costs and Expenses incurred by Applied instituting litigation or taking
other  remedial  measures  under  Section  7.4(g)(i),  (ii)  or  (iii)  shall  be  the
responsibility of Applied.  All recoveries obtained by Applied resulting

(ii)

(iii)

(iv)

18

from such litigation or other appropriate action under Section 7.4(g)(i), (ii)
or (iii) shall be retained by Applied.

(h)

Use of Names.  Subject to Section 12.6, no right, expressed or implied, is granted
by this Agreement to a Party to use in any manner the name or any other trade name of the other
Party or its Affiliates in connection with this Agreement.

(i)

Advanz  Product  Promotional  Materials.    Upon  Applied’s  request,  Advanz  will
provide  to  Applied  samples  of  relevant  marketing,  advertising,  promotional,  training  and
educational  materials  solely  for  the  Product  that  are  developed  by  or  on  behalf  of  Advanz  or  its
Affiliates or Sublicensees in the Territory.  Applied may adapt such materials for use outside of the
Field  or  Territory  to  the  extent  that  such  materials  are  in  Applied’s  control.    In  the  event  that
Applied intends to use such materials (or adaptation thereof) outside of the Field of Territory, the
Parties  will  negotiate  in  good  faith  a  sublicensable  license  to  such  materials  on  commercially
reasonable terms.

(j)

Applied  Product  Promotional  Materials.    Upon  Advanz’s  request,  Applied  will
provide  to  Advanz  samples  of  relevant  marketing,  advertising,  promotional,  training  and
educational materials solely for the Product that are developed by or on behalf of Applied or its
Affiliates or Sublicensees outside the Territory.  Advanz may adapt such materials for use in the
Field in the Territory to the extent that such materials are in Advanz’s control.  In the event that
Advanz  intends  to  use  such  materials  (or  adaptation  thereof)  in  the  Field  in  the  Territory,  the
Parties  will  negotiate  in  good  faith  a  sublicensable  license  to  such  materials  on  commercially
reasonable terms.

SECTION 8. MANUFACTURE AND SUPPLY.

8.1

Commercial  Supply  of  Product.    Applied  shall  Manufacture,  or  shall  have
Manufactured, and supply, and, subject to Sections 8.12 to 8.14, Advanz shall purchase solely from
Applied, Advanz’s and its Affiliates’ and Sublicensees’ requirements of:

(a)

(b)

Bulk Product; and

[***] flavoring packaged separately (i.e., unmixed).

In each case, for patient end use in the Field in the Territory pursuant to and in accordance
with  this  Agreement  and  the  Quality  Agreement.    Subject  to  Section  8.6(d),  Advanz  shall  be
responsible  for  Secondary  Packaging  and  Release  for  the  Product  for  use  in  the  Field  in  the
Territory,  including  all  specialty  pharmaceutical  services,  logistics  and  distribution.    If  Advanz’s
Step-In  Rights  are  exercised  in  accordance  with  Section  8.14,  Applied  shall  reasonably  assist
Advanz  in  procuring  that  Applied’s  Bulk  Product’s  contract  manufacturer  enters  into  a  quality
agreement with Advanz with respect to such supply arrangements.

8.2

Applied Manufacturing Activities.  Except as otherwise expressly set forth herein,
as between the Parties, Applied shall have the sole authority and exclusive right to Manufacture the
Compound and Bulk Product.  Subject to Section 8.9, Applied shall ensure that the Bulk Product
hereunder  for  supply  to  Advanz  complies  with  Applicable  Laws,  cGMP  and  the  Regulatory
Approvals for the Bulk Product for use in the Field in the Territory, including the

18

Product  Specifications;  provided  that  Advanz  shall  comply  with  all  handling,  storage  and  other
requirements under Applicable Laws and the Regulatory Approvals from and delivery to Advanz
of Bulk Product by Applied.  Applied shall have no responsibility or liability to Advanz hereunder
for any non-compliance arising from the acts or omissions of Advanz, its Affiliates or sublicensees
from the point of delivery to Advanz.

8.3

Inspections and Audits.  Upon reasonable notice and during regular business hours,
Advanz  or  its  designee  and/or  any  Regulatory  Authority  or  its  designee  may  inspect  Applied’s
Facilities  and  audit  Applied’s  records,  to  confirm  Applied’s  compliance  with  this  Agreement
(including  Applied’s  allocation  of  stock  of  Bulk  Product  under  Section  8.10)  and  to  ensure
compliance with cGMP and Applicable Laws to the extent they relate to the Product for use in the
Field  in  the  Territory.   Applied  shall  also  grant  Advanz  and  its  designees  and/or  any  Regulatory
Authority  or  its  designees  reasonable  access  to  Applied’s  business  and  operations  personnel
involved in the performance of this Agreement during normal business hours for such foregoing
purposes.  Except where any audit is required by a Regulatory Authority or is an audit initiated by
Advanz on account of Applied’s actual or alleged material breach of this Agreement, such audits
may be conducted by Advanz no more than once annually, unless any such audit reveals a material
noncompliance with cGMP or Applicable Laws, in which case a follow-up audit may be conducted
to ensure that such noncompliance has been satisfactorily remedied.  Advanz’s and any Regulatory
Authority’s rights of audit and inspection in this Section 8.3 shall also apply in respect to Applied’s
Bulk  Product  contract  manufacturer  and  Applied  shall  ensure  that  terms  substantially  similar  to
those  set  out  in  this  Section  8.3  are  contained  in  its  agreement  with  its  Bulk  Product  contract
manufacturer.    Audits  initiated  by  Advanz  under  this  Section  8.3  or  requested  by  a  Regulatory
Authority shall be at Advanz’s sole expense.  If Applied ceases to be a publicly listed company,
Advanz reserves the right to require additional financial audit rights are added to this Section 8.3.

8.4

Forecasting and Ordering.

(a)

Forecasts; Purchase Orders.  At least [***] prior to the first requested delivery date
for Bulk Product, Advanz shall deliver to Applied Advanz’s [***] projection of the quantities of
Bulk  Product  that  Advanz  anticipates  ordering  from  Applied  pursuant  to  this  Agreement  for  the
[***]  commencing  with  the  first  Calendar  Quarter  that  includes  the  first  requested  delivery  date
(the “Initial Forecast”), together with a firm purchase order (a “Purchase Order”) for Bulk Product
for the first [***] covered by such Initial Forecast.  The quantities of Bulk Product specified for the
following [***] of such Initial Forecast shall be non-binding.  Thereafter, [***] prior to the first
Business  Day  of  each  subsequent  Calendar  Quarter  during  the  Term,  Advanz  shall  deliver  to
Applied a rolling [***] forecast updating the prior forecast (together with the Initial Forecast, each
a “Forecast”), together with a Purchase Order for the first [***] of such Forecast.  The quantities of
Bulk  Product  specified  for  the  following  [***]  of  such  Forecast  shall  be  non-binding.    Unless
agreed separately between the Parties in writing, each Purchase Order shall specify no more than
one (1) delivery date for the Bulk Product in each [***].  Purchase Orders shall be in writing, and
no  verbal  communications  shall  be  construed  to  mean  a  commitment  to  purchase  or  sell.    Each
Purchase Order delivered by Advanz to Applied pursuant to this Section 8.4(a) shall be binding on
Applied, unless such Purchase Order exceeds the Initial Forecast by more than [***]of quantity of
Bulk Product, in which case Applied may notify Advanz in writing of its rejection in respect of the
quantity in excess of the Initial Forecast within [***] of receipt of such Purchase Order.

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(b)

Long  Range  Capacity  Planning.    Concurrent  with  the  Initial  Forecast,  for  the
purposes  of  discussion  and  planning  of  Manufacturing  capacity,  Advanz  shall  provide  a  non-
binding forecast of its projected Bulk Product needs for the [***] following that specified in the
Initial  Forecast  as  described  in  Section  8.4(a)  (a  “Long  Range  Forecast”).    Each  Long  Range
Forecast  shall  be  deemed  to  be  revised  by  any  subsequent  Long  Range  Forecast.    In  the  event
Applied  anticipates  that  it  will  be  unable  to  supply  the  quantities  of  Bulk  Product  reflected  in  a
Long Range Forecast, Applied shall promptly notify Advanz and the Parties shall work to remedy
the shortfall in accordance with and subject to the terms of this Section 8 in an effort to assure that
the necessary capacity exists.  Unless otherwise agreed to by the Parties during the Term, the Long
Range Forecast shall be updated by Advanz annually [***] of each Calendar Year during the Term.

(c)

Receipt  and  Acceptance.    Advanz  shall  purchase  all  Bulk  Product  ordered  and
specified in a Purchase Order.  Purchase Orders may be delivered electronically or by other means
to  such  location  as  Applied  shall  designate.    Nothing  in  any  such  Purchase  Order  or  written
acceptance  shall  supersede  or  conflict  with  the  terms  and  conditions  of  this  Agreement  or  the
Quality Agreement.  All Purchase Orders, confirmations of receipt of Purchase Orders and other
notices contemplated under this Section 8.4(c) shall be sent to the attention of such persons as each
Party may identify to the other in writing from time to time in accordance with Section 19.8.

(d)

First-Expiry First-Out.  Advanz shall use Commercially Reasonable Efforts to use
its  inventory  of  Bulk  Product  on  a  first-expiry  first-out  (FEFO)  basis  in  order  to  ensure  that  the
Bulk Product in its inventory always has the maximum period of time remaining on the shelf life.

(e)

Shelf Life.  Applied shall ensure that all Bulk Product has at the date of delivery a

shelf life of the greater of: [***] (“Shelf Life Requirements”).

8.5

(a)

Pricing, Invoicing and Supply Price Reconciliation.

Supply Delivery Price; Invoices.

(i)

Applied has provided Advanz with details of its current COGs together with
an estimate of the COGs for Bulk Product in the first Calendar Year of the
first Launch.  At least [***] preceding the first requested delivery date for
Bulk Product, Applied shall, based on the Initial Forecast and Long Range
Forecast delivered concurrently with the Initial Forecast, update its previous
estimate in good faith of the COGs for Bulk Product for the remainder of the
Calendar Year in which the first Launch occurs.  Thereafter, Applied shall,
based  on  the  then-current  Forecast  and  Long  Range  Forecast,  estimate  in
good  faith  the  COGs  for  Bulk  Product  for  such  successive  Calendar  Year
(being  the  “Estimated  Cost”),  and  shall  notify  Advanz  in  writing  prior  to
[***]  of  each  successive  Calendar  Year  of  such  Estimated  Cost  with:  (y)
reasonable  supporting  documentation  regarding  the  calculation  of  such
Estimated  Costs;  (z)  evidence  to  support  any  increase  in  Estimated  Cost
compared to the then current Estimated Cost.  Any increase in the Estimated
Costs compared to the then current COGs shall be reasonable and evidence-
based.    Should  Applied’s  Bulk  Product  contract  manufacturer’s  costs
decrease, the Estimated Cost shall reflect such decrease accordingly and

18

Applied shall provide the supporting documentation and evidence set out at
(y) and (z) in respect of such decrease.

(ii)

Each  delivery  of  Bulk  Product  under  a  Purchase  Order  hereunder  shall  be
accompanied  by  an  invoice.   Applied  shall  invoice  Bulk  Product  at  [***]
(the  “Total  Supply  Price”).    Advanz  shall  issue  payment  against  such
invoices within thirty (30) days after the end of the calendar month in which
the  invoice  is  received.    Applied  shall  include  the  following  information,
where applicable, on all invoices: the type, description, and quantity of the
Bulk  Product  delivered;  the  date  of  shipment;  the  Total  Supply  Price;  any
applicable taxes, transportation charges or other charges provided for in the
applicable Purchase Order; and the applicable Purchase Order number.

(b)

Taxes.  All Taxes, including, but not limited to, sales, use, excise, value added and
other similar Taxes (but excluding income Taxes and similar Taxes), which Applied is required by
Applicable  Laws  to  collect  from  Advanz  with  respect  to  the  Manufacture  and  supply  of  Bulk
Product  to  Advanz  shall  be  stated  in  Applied’s  invoice  and  shall  be  paid  by  Advanz  to  Applied.
 For the avoidance of doubt, any and all applicable Taxes shall be payable by Advanz in addition to
the Total Supply Price payable on such Bulk Product.

8.6

Shipping, Delivery and Secondary Packaging and Release.

(a)

Delivery.  Applied shall deliver (or have delivered) to Advanz in accordance with
this Section 8.6 the quantities of Bulk Product specified for a given delivery date in each Purchase
Order, except that, without limiting Section 19.1, if Applied provides written notice to Advanz at
least  thirty  (30)  days  prior  to  a  scheduled  date  for  delivery,  Applied  shall  be  permitted  to  delay
delivery for up to fifteen (15) Business Days after the scheduled date for delivery.

(b)

Delivery  Terms.    Bulk  Product  shall  be  supplied  to  [***].    For  the  avoidance  of
doubt,  each  Party  agrees  that  Applied  is  responsible  for  loading  the  Bulk  Product  onto  transport
provided by Advanz or its designated carrier.  Bulk Product shall be shipped at Advanz’s expense
via a carrier reasonably identified by Advanz in the applicable Purchase Order.  Advanz shall be
responsible  for  all  such  shipping  costs,  including  all  freight  and  insurance  charges,  and  for
compliance with all Applicable Laws and Regulatory Approvals for the Product in the Field in the
Territory.

(c)

Retention.    Unless  the  Parties  agree  otherwise,  Applied  shall  maintain  analytical
samples of each batch of Bulk Product (or, if necessary, Compound) in storage for a time period
based upon Applied’s sample retention policy and, in any event, as required by Applicable Laws.

(d)

Secondary Packaging and Release.  Advanz shall be entitled to deduct [***] of its
reasonable Costs and Expenses for all Secondary Packaging and Release activities attributable to a
particular Calendar Quarter which are incurred by Advanz from Royalties prior to payment of the
same by Advanz.  Advanz has provided Applied with details of its current Secondary Packaging
and  Release  costs  together  with  an  estimate  of  such  costs  in  the  first  Calendar  Year  of  the  first
Launch.    At  least  sixty  (60)  days  preceding  the  first  requested  delivery  date  for  Bulk  Product,
Advanz shall update its previous estimate in good faith for Secondary Packaging and

18

Release costs for the remainder of the Calendar Year in which the first Launch occurs.  Thereafter,
Advanz  shall  estimate  in  good  faith  the  Secondary  Packaging  and  Release  costs  for  such
successive  Calendar  Year  (being  the  “Secondary  Packaging  and  Release  Estimated  Cost”),  and
notify  Applied  in  writing  prior  to  September  1st  of  each  successive  Calendar  Year  of  such
Secondary Packaging and Release Estimated Cost with: (y) reasonable supporting documentation
regarding the calculation of such Secondary Packaging and Release Estimated Costs; (z) evidence
to support any increase in Secondary Packaging and Release Estimated Cost compared to the then
current  Secondary  Packaging  and  Release  Estimated  Cost.    Any  increase  in  the  Secondary
Packaging  and  Release  Estimated  Costs  compared  to  the  then  current  Secondary  Packaging  and
Release  Estimated  Cost  shall  be  reasonable  and  evidence-based.    Should  Advanz’s  Secondary
Packaging and Release Costs decrease, the Secondary Packaging and Release Estimated Cost shall
reflect  such  decrease  accordingly  and  Advanz  shall  provide  the  supporting  documentation  and
evidence set out at (y) and (z) in respect of such decrease.

8.7

Certificate of Analysis; Acceptance and Returns.

(a)

Certificate of Analysis; Batch-Tracing; Notice of Non-Conformance.  Applied shall
supply to Advanz the applicable batch number for Bulk  Product delivered, as well as such other
information as the Parties may set forth in the Quality Agreement with respect to Manufacture for
all  Bulk  Product  shipped  to  Advanz  hereunder.    Advanz  will  preserve,  assign  or  link  its  batch
numbers with Applied’s batch numbers in order to comply with Applicable Laws and to ensure its
batch numbers can be traced to Applied’s batch numbers and that such information can and will be
made  available  to  Applied  promptly  upon  request.    In  addition,  Advanz  shall  (within  the  time
period  specified  in  Section  8.7(b))  inspect,  or  cause  to  have  inspected,  each  shipment  of  Bulk
Product  for  any  material  damage,  defect  (including  non-conformance  with  the  Product
Specifications  or  cGMP)  or  shortage  (each  of  the  foregoing,  “Product  Non-Conformance”)  and
give Applied written notice thereof (a “Notice of Non-Conformance”).

(b)

Rejection; Latent Defects.

(i)

(ii)

(iii)

Advanz  shall  have  [***]  following  its  receipt  of  each  shipment  of  Bulk
Product to inspect such shipment.  If Advanz determines that all or any part
of a shipment of Bulk Product suffers from any Product Non-Conformance
in  any  material  respect,  it  shall  provide  Applied  a  Notice  of  Non-
Conformance  in  compliance  with  the  procedures  set  forth  in  the  Quality
Agreement(s).

Latent defects shall be communicated to Applied, together with appropriate
detail,  within  [***]  of  the  date  on  which  such  latent  defect  was  first
discovered by Advanz.

Failure to provide such written notice within such time periods specified in
this  Section  8.7(b),  as  applicable,  shall  be  deemed  acceptance  of  such
shipment  of  Bulk  Product  by  Advanz,  and  Applied  shall  have  no
responsibility or liability to Advanz therefor in respect of any such Product
Non-Conformance.

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(c)

Disputes.  If Advanz delivers a Notice of Non-Conformance in respect of all or any
part of a shipment of Bulk Product, and Applied does not agree with Advanz’s determination that
such  shipment  suffers  from  any  Product  Non-Conformance  in  any  material  respect  (a  “Non-
Conformance Dispute”), the Parties shall in good faith attempt to resolve such Non-Conformance
Dispute  through  qualified  representatives.    The  Non-Conformance  Dispute  shall  be  resolved
between such representatives within [***], unless otherwise agreed in writing by the Parties, from
the date of Applied’s receipt of a Notice of Non-Conformance to resolve such Non-Conformance
Dispute.  If such Non-Conformance Dispute is not resolved by such representatives in such [***]
period,  then  Applied  shall  prepare  an  investigative  report  concerning  such  alleged  Product  Non-
Conformance  and  such  investigative  report  and  Advanz’s  original  Notice  of  Non-Conformance
shall  be  submitted  to  an  independent  testing  laboratory  accepted  by  both  Parties  with  relevant
expertise relating to manufacture and supply of pharmaceutical products.  The laboratory shall be
provided  with  copies  of  Applied’s  investigative  report,  Advanz’s  original  Notice  of  Non-
Conformance,  and  any  response  Advanz  may  provide  to  Applied’s  investigative  report  (which
response shall be provided within seven (7) days of receipt of such investigative report), and shall
be  final  and  binding  on  the  Parties.    If  such  Bulk  Product  is  determined  to  meet  the  Product
Specifications  (or  is  otherwise  determined  not  to  suffer  from  any  Product  Non-Conformance,  as
applicable)  in  all  material  respects,  then  Advanz  shall  pay  for  the  costs  of  such  consultant,  and
shall promptly reimburse Applied for such reasonable out-of-pocket expenses as Applied incurred
in preparing its investigative report in response to the original Notice of Non-Conformance.

(d)

Remedies.  In the event any shipment of Bulk Product is rejected pursuant to this
Section  8.7  as  a  result  of  any  act  or  omission  of  Applied,  its  Affiliates  or  its  their  suppliers  or
contractors, then Advanz shall at its option, as its only remedies (other than with respect to latent
defects),  either:  (i)  destroy  such  rejected  Bulk  Product  at  Applied’s  expense  (in  accordance  with
Applicable Laws); or (ii) return such rejected Bulk Product to Applied or its designee, at a location
designated by Applied and at Applied’s expense.  Advanz shall notify Applied in writing promptly
of the remedy it wishes to claim and Applied shall (at Advanz’s option and sole discretion) either
(iii) promptly replace such non-conforming Bulk Product (or short shipment); or (iv) give Advanz
a credit in an amount equal to the amount paid or payable by Advanz with respect to such rejected
Bulk  Product  (or  short  shipment)  including  in  relation  to  any  commercial  or  tender  penalties
(which  shall  be  limited  to  [***]  in  each  Calendar  Year)  to  which  Advanz  may  be  subject.
  Notwithstanding  the  foregoing  and  in  accordance  with  Section  1.156(k),  Advanz  shall  use
Commercially  Reasonable  Efforts  to  work  with  any  Secondary  Source  Site  approved  in  the
Marketing  Authorization  and  use  its  safety  stock  in  order  to  mitigate  any  commercial  or  tender
penalties to which Advanz may be subject.

8.8

Product  Specification  and  Manufacturing  Changes.    Each  Party  shall  promptly
notify the other Party in writing of any request or order received by a Party from a Governmental
Authority requiring a change to the Product Specifications and/or Manufacturing.  Subject to the
Quality Agreement, Applied shall be responsible for conveying any such changes to its applicable
suppliers, to the extent such changes relate to the Product Specifications or Manufacturing of Bulk
Product;  provided  that  Advanz  shall  be  responsible  for  implementing,  and  shall  comply  at  all
times,  with  any  changes  in  respect  of  the  Secondary  Packaging  and  Release  of  Bulk  Product
supplied to Advanz hereunder, including all specialty pharmaceutical services, including logistics
and distribution responsibilities.

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8.9

Contract  Manufacturer  Terms;  Changes  to  Supply  Terms  Required  by  Regulatory
Approvals and Applicable Laws.  Advanz acknowledges and agrees that (a) the Product remains a
product  in  development,  subject  to  change,  including  as  to  the  requirements  set  forth  in  this
Section  8,  and  is  subject  to  change  as  reasonably  required  by  any  Regulatory  Approval  and
Manufacturing requirements; and (b) subject to Advanz’s exercise of its rights under Sections 8.12
through  8.14  (inclusive),  Applied  shall  take  full  responsibility  for  the  supply  obligations  of  the
Bulk  Product  including  enforcing  the  terms  of  any  applicable  supply  agreement(s)  (at  Applied’s
expense) with respect to the Bulk Product.

8.10

Equal  Priority  to  Available  Bulk  Product  Between  the  Parties.    Subject  to
Section 8.13, each Party acknowledges and agrees that, in the event of a shortage of Bulk Product,
the Parties will share any deficiencies in their supply requirements ratably in accordance with their
volumes for the four (4) Calendar Quarters prior to the Calendar Quarter in which the then-current
shortage first commenced.

8.11
inventory of:

Inventory Stock and Safety Stock.   Applied  shall  maintain  the  following  levels  of

(a)

the  Bulk  Product’s  components  at  all  times  to  meet  the  equivalent  of  [***]  of

Advanz’s most recent forecast (the “Inventory Stock”); and

(b)

inventory  Bulk  Product  at  all  times  to  meet  the  equivalent  of  [***]  of  Advanz’s

most recent forecast (the “Safety Stock”),

provided that such Safety Stock shall not be subject to the Shelf Life Requirements until such time
as  Applied  has  registered  a  shelf  life  of  [***]  in  respect  of  the  Bulk  Product,  at  which  point  all
inventory Bulk Product shall have a minimum shelf life of [***].

8.12

Secondary Source Site.  At any time after the Effective Date, Advanz shall have the
right  to  establish  a  reliable  Third  Party  contract  manufacturer  as  a  secondary  source  site  for
Manufacture  of  the  Bulk  Product  requirements  under  this  Agreement  (the  “Secondary  Source
Site”)  for  use  only  in  the  case  of,  and  duration  of,  (subject  to  Section  8.14)  a  Supply  Shortage.
 Advanz shall notify Applied in writing if it wishes to establish a Secondary Source Site.  Applied
shall provide all reasonable assistance to Advanz (and/or any Third Party) in the establishment of
the  Secondary  Source  Site,  including  providing  all  of  its  then-existing  data  and  information
reasonably  requested  by  Advanz  to  facilitate  the  technology  transfer  of  the  Product  to  an
alternative contract manufacturer and to enable Advanz to fulfil the Manufacturing requirements of
any Regulatory Authority in the Territory.  The Parties shall cooperate reasonably and in good faith
to facilitate the establishment of a Secondary Source Site including any technology transfer.  [***]

8.13

Supply  Shortage.    Subject  to  Section  19.1  and  without  limiting  Section  8.7(d),  if
[***] (a “Supply Shortage”), Applied shall notify Advanz immediately in writing and the Parties
shall discuss a resolution of the Supply Shortage, which may include exercise of Advanz’s Step-In
Rights  under  Section  8.14(b)  such  that  Advanz  may  use  Commercially  Reasonable  Efforts  to
mitigate  any  Supply  Shortage.    In  the  event  of  a  Supply  Shortage,  Advanz  may  also,  in  its  sole
discretion, as its only remedies, notify Applied that it intends to exercise its: (a) Step-In Rights set

18

out in Section 8.14(b); (b) rights to use the Secondary Source Site in accordance with Section 8.12;
and/or (c) claim direct damages for breach of contract in accordance with this Agreement.

Notwithstanding the foregoing and in accordance with Section 1.156(k), Advanz shall use
Commercially  Reasonable  Efforts  to  work  with  any  Secondary  Source  Site  and  use  any  of  its
safety stock approved in the Marketing Authorization in order to mitigate any damages for breach
of contract.

8.14

Step-In Rights.

(a)

In  the  event  of  any  of  the  following:  (i)  the  commencement  of  a  voluntary  or
involuntary bankruptcy proceeding by or against Applied in the United States (provided that, in the
case  of  an  involuntary  bankruptcy  proceeding,  such  proceeding  has  remained  undismissed  or
unstayed  for  a  period  of  sixty  (60)  days),  (ii)  where  and  to  the  extent  agreed  as  part  of  a  FM
Continuity Plan under Section 19.1, (iii) where Section 16.3(a)  is  triggered,  or  (iv)  where  and  to
the extent agreed as  part  of  a  Continuity  Plan  under Section 19.17,  Advanz  shall  have  the  right,
following  service  of  a  Step-In  Notice,  to  continue  any  activities  undertaken  by  Applied  or  any
other Person on Applied’s behalf or required to be undertaken by Applied or any other Person on
Applied’s behalf, in each case, relating to or associated with the Exploitation of the Product for use
in the Field in the Territory (including in relation to Development and Manufacture of the Product)
in accordance with this Agreement.

(b)

In the event of a Supply Shortage, Advanz shall have the right, following service of
a Step-In Notice, to continue Manufacture of the Bulk Product for use in the Field in the Territory
in accordance with Sections 8.12 and 8.13.

(c)

Upon,  and  to  the  extent  necessary  for,  Advanz’s  exercise  of  its  applicable  Step-In
Rights  pursuant  to  Section 8.14(a)  or  8.14(b),  (i)  Applied  shall  provide  copies  of  any  reports  or
other material forming part of the Applied Technology including those required for any Regulatory
Filing related to the Product (e.g., Dossiers, Required Existing Studies, Required Post-MA Studies
and,  subject  to  Section 4.3(d),  Other  Post  Approval  Studies  conducted  by  Applied)  to  the  extent
not already in Advanz’s possession or control, and (ii) Advanz shall have the right to request, and
upon the commencement by Applied of any bankruptcy proceeding allowing Step-In Rights under
Section  8.14(a)  shall  immediately  and  without  further  action  be  deemed  to  have  received
immediately  prior  to  the  commencement  of  any  such  proceeding,  a  temporary  non-exclusive
license under Applied’s Third Party License rights to enable continued Exploitation of such rights
in  accordance  with  Section 8.14(a)  and  under  Applied’s  Third  Party  License  rights  and/or  Third
Party  contract  manufacturing/supply  agreement(s)  to  enable  Advanz’s  Manufacture  of  the  Bulk
Product  by  such  Third  Party  contract  manufacturer  or  at  any  Secondary  Source  Site  (where
applicable);  provided  that,  if  (x)  Advanz  has  exercised  its  Step-In  Rights  due  to  an  applicable
bankruptcy  proceeding  under  Section 8.14(a)  and/or  more  than  twice  in  any  two  (2)  year  period
under Section 8.14(b), or (y) any Supply Shortage lasts for more than twelve (12) months, Advanz
shall  have  the  right  to  request,  where  practicable,  the  partial  assignment  of  Third  Party  License
rights  or  Applied’s  Third  Party  contract  manufacturing/supply  agreement(s)  (or,  where  any
agreement is solely with respect to the Product in the Field in the Territory, complete assignment)
to enable such continued Exploitation or Manufacture, as applicable (the foregoing with respect to
Third Party agreements, “Requested Actions”).  In furtherance of the foregoing subsection (ii),

18

where any Third Party License or Third Party contract manufacturing/supply agreement(s) enables
any  sublicensee  to  enter  into  a  direct  contract  with  the  Third  Party  licensor  or  contract
manufacturer, Applied shall provide all reasonable assistance to Advanz in effecting such transfer.
 Additionally,  Applied  shall  provide  all  reasonable  assistance  to  Advanz  (and/or  any  Third  Party
designated  by  Advanz)  while  Advanz  is  seeking  the  Requested  Actions  or  its  own  contract  with
such  Third  Parties,  including  providing  access  to  Applied’s  then  existing  data,  information,
personnel,  sites,  manufacturers  and  suppliers,  in  each  case,  to  the  extent  reasonably  required  to
facilitate the Manufacture of the Bulk Product for an in-full and on-time delivery of Product for the
Field in the Territory.  Applied agrees to take all steps necessary to ensure that its manufacturers,
suppliers, employees, agents and advisors comply with this provision to enable Advanz to exercise
its Step-In Rights.  Applied shall be entitled to resume Manufacture once Applied has reasonably
demonstrated that it is able to supply Bulk Product in accordance with the terms of this Agreement.

8.15

Effect of Secondary Source Site and Step-in on Royalties.  If Advanz:

(a)

issues  a  Step-In  Notice  during  Development  in  accordance  with  Section  8.14(a),
Advanz shall be entitled to off-set Costs and Expenses incurred in establishing its Step-In Rights
with  respect  to  Development  from  any  remaining  Event  Milestone  Payments  and/or  any  future
Royalties; and

(b)

establishes  its  Secondary  Source  Site  as  a  result  of  a  Supply  Shortage  and/or
otherwise issues a Step-In Notice including after Development in accordance with Section 8.14(a),
Advanz  shall  be  entitled  to  deduct  any  Costs  and  Expenses  incurred  either  from  establishing  its
Secondary  Source  Site  or  if  not  already  established,  from  establishing  a  Manufacturing
arrangement  with  a  reputable  third  party  contractor  pursuant  to  Section 8.12,  in  each  case,  from
Royalties  owed  to  Applied,  including  [***]  of  Costs  and  Expenses  relating  to  Secondary
Packaging and Release in accordance with Section 8.6(d).  [***]

(c)

For clarity, Applied will provide assistance, relevant data, rights to Applied Patent
Rights,  Applied  Technology  and  tech  transfer  in  accordance  with  Sections  8.12  and  8.14,  and
Advanz’s  rights  to  Costs  and  Expenses  incurred  to  establish  Manufacturing,  Development  and
other  Exploitation  arrangements  for  Step-In  Rights,  including  with  third  party  contract
manufacturers  and  Development  and  other  Exploitation,  deducted  from  Royalties  in  accordance
with this Section 8.15, includes Costs and Expenses with respect to specialized/bespoke equipment
but excludes other equipment, software, processes or personnel.

SECTION 9. FINANCIAL PROVISIONS

9.1

Upfront Payment.  Advanz shall pay to Applied the non-refundable, non-creditable
amount  of  Ten  Million  Euros  (€10,000,000)  in  immediately  available  funds,  wired  to  Applied
using the wiring instructions provided by Applied in writing to Advanz, within ten (10) Business
Days after the Effective Date.

18

9.2

Event Milestone Payments.

(a)

Subject to the terms and conditions of this Agreement, Advanz shall pay to Applied
the amount set forth in the table below opposite the corresponding event milestone (each an “Event
Milestone”) as a non-refundable, non-creditable amount paid in accordance with Section 10.4.

Event Milestone
Successful  Completion  of  the  AT-007-1002
Study, where “Successful Completion” means
[***]

Event Milestone
Payment
[***]

Successful  Completion  of  the  AT-007-1005
Study, where “Successful Completion” means
[***]

a 

of 

Grant 
centralized  Marketing
Authorization  by  the  EMA  allowing  sale  of
the  Product  in  the  Territory  for  use  in
Marketing
Galactosemia, 
Authorization  may 
conditional
authorization  or  authorization  with  respect  to
a sub-population of patients

which 
be 

a 

a 

of 

Grant 
centralized  Marketing
Authorization  by  the  EMA  allowing  sale  of
the Product in the Territory for use in SORD,
which  Marketing  Authorization  may  be  a
conditional  authorization  or  authorization
with respect to a sub-population of patients

Annual  Net  Sales  for  the  Product  in  the
Territory  exceeds  [***]  in  a  Calendar  Year
(“Commercial Event Milestone 1”)

Annual  Net  Sales  for  the  Product  in  the
Territory  exceeds  [***]  in  a  Calendar  Year
(“Commercial Event Milestone 2”)

18

[***]

[***]

[***]

[***]

[***]

Payable
Within fifteen (15)
Business Days from
the date of receipt of
the invoice
applicable to such
Event Milestone
Payment

Within fifteen (15)
Business Days from
the date of receipt of
the invoice
applicable to such
Event Milestone
Payment

Within fifteen (15)
Business Days from
the date of the
occurrence of such
Event Milestone

Within fifteen (15)
Business Days from
the date of
occurrence of such
Event Milestone

Subject to
Section 9.2(b)(iii)(B)

Subject to
Section 9.2(b)(iii)(B)

Event Milestone
Annual  Net  Sales  for  the  Product  in  the
Territory  exceeds  [***]  in  a  Calendar  Year
(“Commercial Event Milestone 3”)

Annual  Net  Sales  for  the  Product  in  the
Territory  exceeds  [***]  in  a  Calendar  Year
(“Commercial Event Milestone 4”)

Event Milestone
Payment
[***]

Payable
Subject to
Section 9.2(b)(iii)(B)

[***]

Subject to
Section 9.2(b)(iii)(B)

(b)

For the avoidance of doubt: (i) each Event Milestone Payment shall be payable only
on  the  first  occurrence  of  the  corresponding  Event  Milestone;  (ii)  no  Event  Milestone  Payment
shall be payable more than once; (iii) in respect of the Commercial Event Milestones: (A) should a
subsequent Commercial Event Milestone occur before a prior Commercial Event Milestone, then
all  such  preceding  Commercial  Event  Milestone  Payments  shall  be  due  and  payable  on  the
occurrence of such later Commercial Event Milestone (e.g., if Advanz achieves Commercial Event
Milestone  4  in  the  first  Calendar  Year  of  this  Agreement,  the  Commercial  Event  Milestone
Payments  for  Commercial  Event  Milestone  1,  Commercial  Event  Milestone  2  and  Commercial
Event Milestone 3 shall become due and payable); (B) at the end of each Calendar Year, Advanz
shall provide Applied with its Annual Net Sales figures within thirty (30) days of the end of the
Calendar Year; if Advanz has achieved any Commercial Event Milestone, Applied shall issue an
invoice which shall be payable by Advanz within thirty (30) days of receipt of such invoice; and
(C)  Advanz  will  report  Net  Sales  relating  to  Commercial  Event  Milestones  at  the  end  of  each
Calendar Quarter.

(c)

NOTWITHSTANDING  THIS  SECTION  9.2,  APPLIED  MAKES  NO
REPRESENTATION OR WARRANTY, EITHER EXPRESS OR IMPLIED, THAT IT WILL BE
ABLE  TO  SUCCESSFULLY  DEVELOP,  OR  THAT  ADVANZ  WILL  BE  ABLE  TO
SUCCESSFULLY COMMERCIALIZE, THE PRODUCT.

9.3

Royalties on Net Sales.  Subject to the terms hereof, and on and from the Effective
Date and for the duration of the Initial Royalty Term, in addition to any applicable Event Milestone
Payments,  Advanz  shall  pay  to  Applied  royalties  on  Annual  Net  Sales  of  Product  for  use  in  the
Field in the Territory (the “Royalties”) at a rate of twenty percent (20%).  Upon expiration of the
Initial Royalty Term and for the duration of the Term, Advanz shall pay to Applied Royalties at a
rate  of  [***]  of  Net  Sales.    [***]  of  any  Costs  and  Expenses  to  the  extent  related  to  Secondary
Packaging  and  Release  which  are  incurred  by  Advanz  shall  be  deducted  from  Royalties  prior  to
payment by Advanz in accordance with Section 8.6(d).

SECTION 10.ACCOUNTING AND PROCEDURES FOR PAYMENT

10.1

Periodic Reporting and Reconciliation Payments.

(a)

Royalty Reports; Payments.  Within thirty (30) days after the end of any Calendar
Quarter, Advanz shall provide Applied with a report stating the Net Sales and computation thereof
(including  gross  sales  in  units  and  in  value  of  the  Product  made  by  or  on  behalf  of  Advanz,  its
Affiliates,  and  Sublicensees,  as  applicable,  in  the  Territory,  and  any  permitted  deductions  in
accordance with the definition of Net Sales), on a Country-by-Country basis, during such

18

preceding  Calendar  Quarter,  together  with  the  calculation  of  the  Royalties  due  to  Applied,
including the method used to calculate the Royalties, and the exchange rates used (together with
any other supporting documentation and additional information reasonably requested by Applied,
including detailed information reasonably necessary to permit Applied to verify the accuracy of the
reported  Net  Sales,  including  product  names,  selling  price  (including  gross  selling  price  where
available), country where Manufactured (to the extent Bulk Product is Manufactured pursuant to
Advanz’s  Step-In  Rights  under  Section  8.14  or  pursuant  to  Section  16.3(a))  and  country  of
Secondary Packaging and Release).  Royalty payments relating to such quarterly reports shall be
made by Advanz within thirty (30) days following receipt of Applied’s invoice.  Advanz shall also
provide  an  equivalent  report  upon  the  achievement  of  any  Event  Milestones  triggering  an  Event
Milestone Payment.  Upon the request of Applied and to the extent reasonably practicable, Advanz
shall  cooperate  with  Applied  in  providing  assistance  with  qualitative  feedback  to  assist  Applied
derive the information required under a Third Party License with respect to Net Sales with respect
to each Licensed Indication.

(b)

Reimbursement  Payments.    Where  either  Party  is  required  to  reimburse  the  other
Party  in  accordance  with  the  terms  of  this  Agreement  [***]  then  the  Party  to  whom  such
reimbursement  is  owed  may,  on  a  monthly  basis,  send  an  invoice  to  such  other  Party  (the
“Reimbursing Party”) with respect to such reimbursable amounts, along with reasonable evidence
thereof, and such Reimbursing Party shall issue payment against such invoices within thirty (30)
days after the end of the calendar month in which the invoice is received.

10.2 Disputes.    In  the  event  of  a  dispute  regarding  any  amount  reported  by  Advanz
pursuant to Section 10.1, Applied shall provide a notice of the dispute to Advanz, and the Parties
will promptly meet and negotiate in good faith a resolution to such dispute.  In the event that the
Parties  are  unable  to  resolve  such  dispute  within  thirty  (30)  days  after  notice  by  Applied,  either
Party  may  refer  such  matter  to  be  determined  by  the  dispute  resolution  procedures  set  forth  in
Section 18.3.

10.3 Currency.  Save for the Total Supply Price, all payments to be made hereunder by
one  Party  to  the  other  Party  shall  be  computed  and  paid  in  Euros  (€).   As  it  relates  to  the  Total
Supply Price, payments to be made hereunder shall be computed and paid in United States dollars
(USD).

10.4 Method of Payments.  Each payment to be made hereunder by Advanz to Applied
shall be made by electronic transfer in immediately available funds via either a bank wire transfer,
an ACH (automated clearing house) mechanism, or any other means of electronic funds transfer, at
Applied’s election, to the account designated (in writing) by Applied on or before the due date set
out  in  Section  9,  Section  10.1  or  otherwise  in  this  Agreement.    With  respect  to  any  payment
invoiced by Applied to Advanz, Applied may designate a different bank account on such invoice.
 With respect to any other payment, Applied may designate a different bank account at least thirty
(30) days before such payment is due.

10.5

Exportation  of  Funds.    Advanz  shall  be  solely  responsibility  for  procuring  any
required permits, authorizations, licenses or consents of Governmental Authorities for the export of
funds as may be required in the Territory; provided, however, that to the extent that it is impossible
to make such payments due to the “blocking” of funds by Applicable Laws, such

18

“blocked”  funds  shall  be  deposited  to  the  credit  of  Applied  in  such  depository  as  Applied
designates subject to such Applicable Laws or Advanz or its Affiliates shall otherwise pay Applied
an amount equal to such “blocked” funds.

10.6 No  Set-Off.    Subject  to  Section  8.15,  all  payments  which  Advanz  is  required  to

make under this Agreement shall be made without any set-off, counterclaim or condition.

10.7

Interest  for  Late  Payments.    If  either  Party  fails  to  make  any  undisputed  payment
due under this Agreement within thirty (30) days of the date upon which such undisputed payment
is due, then interest shall accrue on such payment on a daily basis from the date such payment was
originally due at a rate equal to Secured Overnight Financing Rate (SOFR) (as published in The
Wall Street Journal, New York edition) plus two percent (2%), or at the maximum rate permitted
by Applicable Laws, whichever is the lower, and such interest shall be paid when such payment is
made.

10.8

Inspection of Records.  Advanz shall, and shall cause its Affiliates and Sublicensees
to, keep accurate books and records with respect to the Commercialization (and other Exploitation
under Advanz’s control as a result of Advanz exercising its Step-In Rights) hereunder, including
setting  forth  gross  sales  of  the  Product  and  Net  Sales  sufficient  to  enable  the  calculation  of
amounts payable hereunder to be verified.  Advanz will retain such books and records for five (5)
years after the end of the Calendar Year in which they are generated (or such longer period as may
be  required  by  Applicable  Laws)  in  order  to  enable  audit  of  such  records  as  set  forth  below.
 Applied shall appoint an independent Third Party (approved in advance by Advanz and subject to
a reasonably acceptable confidentiality agreement) to examine Advanz’s books and records at any
reasonable  time,  upon  reasonable  notice  and  at  the  facility(ies)  where  the  books  and  records  are
normally kept (an “Audit”) in order to verify Advanz’s compliance with the terms and conditions
hereof and the calculation of amounts payable hereunder.  The foregoing right of examination may
be exercised only once during each twelve (12)-month period of the Term, unless (a) a prior Audit
has  revealed  a  discrepancy  demonstrating  an  underpayment  by  Advanz  of  five  percent  (5%)  or
more, in which case Applied may conduct such additional Audits as may be reasonably required to
ensure such discrepancy has been cured and/or has not reoccurred, or (b) Applied otherwise has a
good  faith  reason  to  believe  that  Advanz  may  be  in  breach  of  the  terms  and  conditions  hereof.
  Advanz  shall  bear  the  Cost  and  Expense  of  any  such  examination  and  review  if  there  is  an
underpayment  by  Advanz  of  five  percent  (5%)  or  more.    If  such  Audit  reveals  that  Advanz  has
made an: (x) underpayment of any payments due to Applied under this Agreement, then Advanz
shall promptly pay Applied the amount of such underpayment or overpayment as was revealed by
such  Audit;  or  (y)  overpayment  of  any  payments  due  to  Applied  under  this  Agreement,  then
Applied shall promptly issue a credit note to Advanz for the amount of such underpayment as was
revealed by such Audit.

10.9

Tax Matters.

(a)

Taxes.  To the extent they are applicable to Advanz, Advanz shall assume and pay
any  and  all  Taxes  (excluding  income  Taxes  and  similar  Taxes),  customs,  duties,  assessments,
excises and other charges levied upon the importation of or assessed against the Products supplied
or  rights  licensed  by  Applied  hereunder,  or  for  or  on  account  of  the  Commercialization  of  the
Product in the Territory.

18

(b)

VAT.  It is understood and agreed between the Parties that any payments made by
Advanz under this Agreement are exclusive of any value added or similar Tax (“VAT”)  imposed
upon such payments.

(c)

Withholding Tax.  To the extent Advanz is required to deduct and withhold Taxes
on  any  payments  to  Applied  hereunder,  the  sum  payable  by  Advanz  (in  respect  of  which  such
deduction  or  withholding  is  required  to  be  made)  shall  be  increased  to  the  extent  necessary  to
ensure  that  Applied  receives  a  sum  equal  to  the  sum  which  it  would  have  received  had  no  such
deduction or withholding Tax been applicable (i.e., the payment to Applied shall be “grossed up”
with sums corresponding to the applicable deduction or withholding Tax, such that the net effect of
such  withholding  Tax  on  Applied  is  zero).   Advanz  shall  pay  the  amounts  of  such  Taxes  to  the
proper  Governmental  Authority  in  a  timely  manner  and  promptly  transmit  to  Applied  an  official
Tax certificate or other evidence of such payment of such deduction or withholding Tax.

(d)

Cooperation.    Each  Party  shall  provide  the  other  with  reasonable  assistance  to
enable  the  recovery,  as  permitted  by  Applicable  Laws,  of  withholding  Taxes,  VAT,  or  similar
obligations  resulting  from  payments  made  under  this  Agreement,  such  recovery  to  be  for  the
benefit  of  the  Party  bearing  such  withholding  Tax,  VAT,  or  similar  obligation.    Applied  shall
provide to Advanz any Tax forms that may be reasonably requested by and necessary for Advanz
not  to  withhold  tax  or  to  withhold  Tax  at  a  reduced  rate  under  Applicable  Laws  (including  an
applicable income Tax treaty).  Each Party further agrees to provide reasonable cooperation to the
other Party, at the other Party’s expense, in connection with any official or unofficial Tax audit or
contest relating to payments made by Advanz to Applied under this Agreement.

SECTION 11.PATENTS AND INFRINGEMENT

11.1

Filing and Prosecution.  Applied shall at its cost, subject to Sections  11.2  through
11.3,  use  Commercially  Reasonable  Efforts  to  obtain,  prosecute  and  maintain  its  Patent  Rights
included in the Applied Patent Rights, including to:

(a)

file Patent Applications on any invention included in the Applied Patent Rights or

Applied Technology (which Patent Applications shall be Applied Patent Rights hereunder);

(b)

prosecute  all  pending  and  new  Patent  Applications  included  within  the  Applied

Patent Rights;

(c)

respond  to  oppositions,  interferences,  nullity  actions,  re-examinations,  inter  pates
reviews,  revocation  actions  and  similar  proceedings  filed  by  Third  Parties  against  the  grant  of
Patents for such Patent Applications; and

(d)

except as set out at (y) below, maintain in force any Patent Rights in the Territory
included within the Applied Patent Rights by duly filing all necessary papers and paying any fees
required by Applicable Laws of the particular Country in which the Patent Right was granted.

Applied shall at its cost, subject to Sections 11.2 through 11.3, (x) reject the competence of
the Unitary Patent Court in respect of any Applied Patent Rights; and (y) maintain and defend the
Patents in the Territory sublicensed to Advanz under this Agreement which are the subject of

18

the Columbia License (the “Columbia Patents”) by duly filing all necessary papers and paying any
fees required by Applicable Laws of the particular Country in which the Patent was granted.

Applied shall be responsible for all the Costs and Expenses it incurs in connection with the actions
taken under this Section 11.1 (subject to Sections 11.2 and 11.3).

11.2 Correspondence.  Applied will keep Advanz informed of the status of the Applied
Patent Rights to the extent the Applied Patent Rights cover the Commercialization of the Product
in the Field in the Territory (but specifically excluding Applied Patent Rights directed solely to an
Out-of-Scope  Product)  solely  to  the  extent  a  change  in  the  status  of  such  Applied  Patent  Rights
could reasonably be expected to impair the Commercialization of the Product in the Field in the
Territory in a material respect.  For clarity, Applied shall have ultimate decision-making authority
with respect to filings and prosecution and maintenance of Applied Patent Rights, and will use its
good faith business judgement in making all such decisions.  If Applied decides not to commence
or  proceed  with  any  filings  or  prosecution  of  its  Applied  Patent  Rights  or  maintenance  of  its
Applied  Patent  Rights  (except  the  Columbia  Patents),  it  shall  advise  Advanz  promptly  of  this
decision.    If  Advanz  decides  it  wishes  to  have  any  such  filings,  prosecution  or  maintenance
continued,  it  shall  notify  Applied  promptly.    Applied  shall  continue  to  use  Commercially
Reasonable  Efforts  to  continue  with  any  such  filings,  prosecution  or  maintenance,  with  Advanz
reimbursing Applied’s Costs and Expenses monthly on an as incurred basis.  Applied shall retain
sole and exclusive ownership of the foregoing.

11.3 Notices.  Applied agrees that it will, and will cause its Affiliates to, execute and file
those notices and other filings as Advanz shall reasonably request be made, from time to time with
any  patent  office  in  the  Territory  with  respect  to  the  rights  granted  under  this  Agreement,  at
Advanz’s sole cost and expense.

11.4

Third Party Royalty Obligations.

(a)

If  either  Party  reasonably  determines  in  good  faith  that  in  order  to  avoid
infringement  or  other  violation  of  any  Patent  Right  not  licensed  hereunder,  it  is  reasonably
necessary  to  obtain  a  license  from  a  Third  Party  in  order  to  Manufacture,  Commercialize  or
otherwise  Exploit  the  Product  in  a  Country  in  the  Territory  and  to  pay  a  royalty  or  other
consideration  under  such  license  (including  in  connection  with  the  settlement  of  a  claim  of
infringement or other violation of Patent Rights), then the Parties shall discuss the pertinent Patent
Right of such Third Party and such Party’s determination.  If the Parties decide that Advanz should
enter  into  such  license,  Advanz  shall  (i)  use  Commercially  Reasonable  Efforts  to  negotiate  and
enter into a license for such Patent Rights of such Third Party on commercially reasonable terms
and  notified  to  Applied  and  (ii)  be  responsible  for  making  any  payments  to  such  Third  Party  in
respect of such license, which shall be reimbursed by Applied on request from Advanz.  If Applied
should enter into such license, Applied shall make any payments to such Third Party in respect of
such license directly.

(b)

If:

(i)

Advanz is subject to a final court or other binding order or ruling requiring
any payments, including the payment of a royalty to a Third Party holder of

18

Patent Rights in respect of sales of the Product in a Country in the Territory;
or

(ii)

Applied is subject to a final court or other binding order or ruling requiring
any payments, including the payment of a royalty to a Third Party holder of
Patent Rights in respect of sales of the Product in a Country in the Territory,
the  amount  of  such  payments  made  a  Party  to  the  Third  Party  holder  of
Patent  Rights  shall  be  shared  equally  between  the  Parties  such  that  (A)  if
Advanz  make  such  payment  [***]  of  such  amount  shall  be  deducted  from
Royalties for such Calendar Quarter in which they are due and payable; and
(B)  if  Applied  makes  such  payment,  Advanz  shall  promptly  reimburse
Applied  in  respect  of  [***]  of  such  amount.    For  clarity,  any  litigation
relating to the foregoing shall be handled as provided in Section 11.6.

11.5

Third-Party Infringement.  Each Party will promptly notify the other in the event of
any actual, potential or suspected infringement or other violation in the Territory of a Patent under
the Applied Patent Rights by any Third Party.

(a)

Infringement  of  Applied  Patent  Rights  in  the  Field.    Subject  to  any  rights  of  an

owner of the Applied Patent Rights under a Third Party License:

(i)

Applied shall have the first right, but not the obligation, to institute litigation
or take other remedial measures in connection with Third Party infringement
or other violation of the Applied Patent Rights occurring in the Field within
the  Territory.    If  Applied  chooses  not  to  initiate  litigation  or  take  other
remedial measures against a Third Party who is alleged to be infringing or
otherwise  violating  the  Applied  Patent  Rights  in  the  Territory  in  the  Field
(other  than  Applied  Patent  Rights  directed  solely  to  an  Out-of-Scope
Product)  within  [***]  of  Advanz’s  request  that  Applied  do  the  same
(provided  that,  if  Applied  intends  to  initiate  such  litigation  or  remedial
measures, Applied shall notify Advanz that it intends to do so with [***] of
Advanz’s request), then Advanz shall have the right to initiate litigation or
take other appropriate action to the extent (A) such Third Party infringement
or other violation would reasonably be expected to impair or has impaired
the Commercialization of the Product in the Field in the Territory (subject to
obtaining  Applied’s  prior  written  approval,  such  approval  not  to  be
unreasonably  withheld,  conditioned  or  delayed)  and  (B)  such  litigation  or
other appropriate action does not conflict with the enforcement rights (and
otherwise  complies  with  the  rights)  of  the  owner  of  any  Applied  Patent
Rights under a Third Party License.  Applied shall notify Advanz promptly
if  it  becomes  aware  that  the  owner  of  any  Applied  Patent  Rights  under  a
Third  Party  License  intends  to  initiate  litigation  or  take  other  appropriate
action.    Each  Party  agrees  to  reasonably  cooperate  with  the  other  in
connection with any such litigation or measures taken by such other Party in
accordance  with  this  Section  11.5(a)(i)  (including,  as  may  be  required,
timely  joining  as  a  party  in  any  such  litigation).   The  Party  initiating  such
litigation or other measures shall bear: (x) all Costs and

18

Expenses;  (y)  any  losses  in  connection  with  any  such  litigation  or  other
measures; and (z) be entitled to retain any recoveries obtained resulting from
any  such  litigation  or  other  measures  after  making  any  payments  to  the
owner of any Applied Patent Right or Applied Technology required under a
Third Party License,  subject to such amounts being evidenced in writing to
Advanz where Advanz is the Party taking the action and bearing the Costs
and  Expenses.  The  Party  initiating  such  litigation  or  other  measures  in
accordance with this Section 11.5(a)(i) shall consult with the other Party as
to the strategy for the same and shall consider in good faith any comments
from  the  other  Party  and  keep  the  other  Party  reasonably  informed  of  any
steps taken with respect thereto.

(ii)

Applied shall have the sole right, but not the obligation, to institute litigation
or take other remedial measures in connection with Third Party infringement
or  other  violation  of  any  Applied  Patent  Rights  occurring  outside  of  the
Territory and with respect to Third Party infringement or other violation of
any  Applied  Patent  Rights  directed  solely  to  any  Out-of-Scope  Product  or
occurring outside the Field (within or outside of the Territory), and any such
litigation or remedial measures shall be at Applied’s sole cost and expense.
 Applied shall retain all recoveries received by Applied and bear all losses
arising  as  a  result  of  its  enforcement  of  Applied  Patent  Rights  under  this
Section 11.5(a)(ii).

11.6 Other Actions by a Third Party.  Each Party shall promptly notify the other in the
event of any (a) claims by a Third Party of alleged infringement or other violation of Patent Rights
by  Advanz  or  Applied  or  any  of  their  respective  Affiliates  or  Sublicensees  with  respect  to  the
Development, Manufacture, Commercialization or other Exploitation of the Product or (b) legal or
administrative  action  by  any  Third  Party  involving  an  Applied  Patent  Right  (other  than  Applied
Patent  Rights  directed  solely  to  an  Out-of-Scope  Product)  of  which  it  becomes  aware,  including
any nullity, revocation, reexamination or compulsory license proceeding.  Subject to any rights of
an  owner  of  the  applicable  Applied  Patent  Rights  under  a  Third  Party  License  and  to
Section 11.1(y), Applied  shall  have  the  first  right,  but  no  obligation,  to  defend  against  any  such
claim  or  action  involving  such  Applied  Patent  Right  in  the  Territory.    If  Applied  chooses  not  to
defend  against  any  such  claim  or  action  involving  an  Applied  Patent  Right  within  [***]  of
Advanz’s  request  that  Applied  do  the  same  (provided  that,  if  Applied  intends  to  undertake  such
defense,  Applied  shall  notify  Advanz  that  it  intends  to  do  so  within  [***]  of  Advanz’s  request),
then  Advanz  shall  have  the  right  to  defend  such  claim  or  action  (to  the  extent  that  such  right  to
defend  does  not  conflict  with  (and  otherwise  complies  with))  the  rights  of  the  owner  of  any
Applied  Patent  Rights  under  a  Third  Party  License.   Applied  shall  notify  Advanz  promptly  if  it
becomes aware that the owner of any Applied Patent Rights under a Third Party License intends to
initiate litigation or take other appropriate action.  Each Party, upon request of the other Party, shall
reasonably  cooperate  with  the  other  Party’s  defense  of  any  such  claims  or  actions  (including,  as
may  be  required,  timely  joining  as  a  party  in  any  such  claim  or  action).    The  Party  defending
against any such claim or action in accordance with this Section 11.6 shall consult with the other
Party as to the strategy for the same and shall consider in good faith any comments from the other
Party  and  keep  the  other  Party  reasonably  informed  of  any  steps  taken  with  respect  thereto.    No
settlement of any such claim or action shall be entered into by a Party (without the written consent

18

of  the  other  Party,  which  shall  not  be  unreasonably  delayed,  conditioned  or  withheld)  if  such
settlement would reasonably be expected to have a material adverse effect on the rights or interest
of  the  other  Party  or  any  of  its  Affiliates  or  impose  any  costs  or  liability  on,  or  involve  any
admission  by,  the  other  Party  or  any  of  its  Affiliates.    In  the  event  Advanz  is  defending  against
such claim or action, Applied shall have the right to join such defense using its own counsel at its
own cost and expense.  The Party defending such litigation or other measures shall bear all Costs
and  Expenses  and  any  losses  in  connection  with  any  such  litigation  or  other  measures  and  be
entitled to retain any recoveries obtained resulting from any such litigation or other measures after
making any payments to the owner of any Applied Patent Right or Applied Technology required
under a Third Party License, subject to such amounts being evidenced in writing to Advanz where
Advanz is the defending Party and provided that, in respect of Section 11.6(a), where either Party
is  subject  to  a  final  court  or  other  binding  order  or  ruling  requiring  any  payments,  including  the
payment of a royalty to a Third Party holder of Patent Rights in respect of sales of the Product in a
Country in the Territory, the amount of such payments made a Party to the Third Party holder of
Patent Rights shall be shared [***] between the Parties such that (x) if Advanz make such payment
[***] of such amount shall be deducted from Royalties for such Calendar Quarter in which they
are  due  and  payable;  and  (y)  if  Applied  makes  such  payment,  Advanz  shall  promptly  reimburse
Applied in respect of [***] of such amount.  

11.7

Patent Marking.  Advanz shall, and shall cause its Affiliates and Sublicenses to, at
Advanz’s  cost  and  expense,  comply  with  the  patent  marking  statutes  of  which  it  is  notified  by
Applied in each Country in the Territory in which the Product is Commercialized by or on behalf
of Advanz hereunder.

SECTION 12.CONFIDENTIALITY; PUBLICATION

12.1 Confidentiality.  Except  to  the  extent  expressly  authorized  by  this  Agreement  or
otherwise agreed in writing by the Parties, the Parties agree that for the Term and for ten (10) years
thereafter,  each  Party  shall  (a)  keep  confidential  and  shall  not  publish  or  otherwise  disclose  any
Confidential Information furnished to it by the other Party pursuant to this Agreement, in a manner
no less protective than the actions it would customarily take to preserve the confidentiality of its
own  similar  types  of  confidential  information,  and  (b)  not  use  for  any  purpose  any  Confidential
Information furnished to it by the other Party other than for the performance of its obligations or
the exercise of its rights hereunder in accordance with the terms hereof.

12.2

Permitted Disclosures.  Notwithstanding the foregoing, each Party may disclose the
other  Party’s  Confidential  Information  (a)  to  such  Party’s  employees,  consultants  (including,  for
greater  certainty,  financial  advisors  and  its  lenders),  Affiliates,  agents,  contractors,  or  permitted
sublicensees who are bound by obligations relating to confidentiality at least as restrictive of those
contained herein and who have a need to know such information in connection with such Party’s
performance of its obligations or practice or enforcement of its rights under this Agreement, (b) to
Regulatory  Authorities  in  connection  with  any  Regulatory  Filings  made  by  either  Party  for
Development, Manufacture,  Commercialization  or  other  Exploitation  of  a  Product in compliance
with Applicable Laws and the terms hereof (inside or outside the Territory, in the case of Applied),
or (c) pursuant to Section 12.3 or 12.4.

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12.3

Terms of Agreement.    The  Parties  agree  that  the  terms  of  this  Agreement  will  be
considered Confidential Information of both Parties.  Subject to Section 12.4 below, no Party shall,
without the prior written consent of the other Party, disclose in any manner to any Third Party the
terms  and  conditions  of  this  Agreement,  except  for  terms  or  subject  matter  which  has  been  the
subject of prior public disclosure or has been mutually approved for such disclosure and except as
set  forth  below.    In  addition:  (a)  either  Party  may  disclose  such  terms  as  are  required  to  be
disclosed in its publicly-filed financial statements, or other public statements or reports, pursuant
to Applicable Laws, regulations or stock exchange rules (e.g., the rules of the U.S. Securities and
Exchange Commission, the NYSE American, the NYSE, NASDAQ, or any other stock exchange
on  which  securities  issued  by  either  Party  may  be  listed)  and  publicly  file  this  Agreement  as  an
exhibit with such report; provided that, such Party shall provide the other Party with a copy of the
proposed text of such statements or disclosure (including any exhibits containing this Agreement)
sufficiently in advance of the scheduled release or publication thereof to afford such other Party a
reasonable  opportunity  to  review  and  comment  upon  the  proposed  text  (including  redacted
versions of this Agreement), (b) either Party shall have the further right to disclose the terms of this
Agreement  under  a  confidentiality  obligation  no  less  protective  than  those  set  forth  in  this
Agreement,  to  any  actual  or  potential  licensee,  sublicensee,  acquirer,  merger  partner,  investor,
business  partner  or  potential  providers  of  financing  and  each  of  their  respective  advisors  or
(c) Applied shall have the right to disclose information to the owner of any Applied Patent Right or
Applied Technology under a confidentiality obligation no less protective than those set forth in this
Agreement to the extent reasonably necessary for Applied to comply with its reporting or notice
obligations under any applicable Third Party Licenses; and (d) Applied and Advanz shall have the
right to disclose information regarding the Development, Commercialization or other Exploitation
status  of  the  Product  in  the  Field  in  the  Territory  to  the  extent  such  disclosure  by  Applied  or
Advanz,  as  applicable,  is  required  by  Applicable  Laws,  regulations  or  stock  exchange  rules;
provided  that,  such  Party  shall  provide  the  other  Party  with  a  copy  of  the  proposed  text  of  such
statements or disclosure (including any exhibits containing this Agreement) sufficiently in advance
of the scheduled release or publication thereof to afford such other Party a reasonable opportunity
to review and comment upon the proposed text (including redacted versions of this Agreement).

12.4 Mandatory Disclosure.

(a)

Notification  and  Consultation.    Except  with  respect  to  disclosures  permitted  by
Section  12.3,  in  the  event  that  a  Party  is  required  by  Applicable  Laws  (including  rules  of  an
applicable  stock  exchange),  or  pursuant  to  legal,  governmental  or  self-regulatory  organization
proceedings (including by court order or judicial or administrative process) to disclose any part of
the other Party’s Confidential Information (including terms or conditions of this Agreement), such
Party shall (i) promptly notify the other Party of each such requirement and identify the documents
so required thereby, so that the other Party may seek an appropriate protective order, confidential
treatment or other remedy concerning any such disclosure or waive compliance by such Party with
the provisions of this Agreement and (ii) consult with the other Party with respect to taking legally
available steps to resist or narrow the scope of such requirement.

(b)

Limited  Disclosure.    If,  in  the  absence  of  such  a  protective  order,  confidential
treatment request, other remedy or waiver by the other Party, such Party is nonetheless required to
disclose any part of the other Party’s Confidential Information or any terms or conditions of this

18

Agreement, such Party may disclose such Confidential Information or terms or conditions without
liability  under  this  Agreement,  except  that  such  Party  shall  furnish  only  that  portion  of  the
Confidential Information or terms or conditions that in its good faith judgment, after consultation
with legal counsel, it is legally required to provide.

12.5

Publication.    Nothing  herein  shall  prevent  Applied  or  its  Affiliates  (or  their
respective employees, consultants, contractors, licensees and agents) from publishing or presenting
information  relating  to  the  Compound  or  Product  or  otherwise  (a)  limit  the  rights  of  Applied’s
Third Party clinical investigators to publish the results of their studies or (b) prevent Applied or its
Affiliates  (or  their  respective  employees,  consultants,  contractors,  licensees,  and  agents)  from
complying with Applicable Laws with respect to the disclosure of clinical study data and results or
of any other material matter or information.  Advanz shall not publish or present any information
relating to the Compound or Product without Applied’s prior written consent.

12.6

Publicity.  The public announcement of the execution of this Agreement is set forth
on Exhibit F attached hereto and shall be promptly disseminated as a press release following the
execution of this Agreement by both Parties.  Each Party shall, if reasonably practicable under the
circumstances, give the other Party sufficient advance notice of at least twenty-four (24) hours of
the text of any public statement concerning the terms of, or events related to, this Agreement or
concerning the Compound or Product so that the other Party will have the opportunity to comment
upon such statement.  Such Party shall give due consideration to any specific reasonable comments
of the other Party on such text timely received from the other Party.

SECTION 13.WARRANTIES

13.1 Mutual Warranties.  Each of Advanz and Applied hereby warrants to the other Party

as of the Effective Date as follows:

(a)

It  is  duly  organized,  validly  existing  and  in  good  standing  under  the  Applicable
Laws  of  the  jurisdiction  of  its  incorporation  or  formation,  as  applicable.    It  has  the  requisite
corporate or other entity power and authority to conduct its business as presently being conducted
and as proposed to be conducted by it.

(b)

It has the requisite corporate or other entity power and authority to enter into this
Agreement  and  to  perform  its  obligations  hereunder.   All  corporate  or  other  entity  actions  on  its
part,  necessary  for  (i)  the  authorization,  execution,  delivery  and  performance  by  it  of  this
Agreement,  and  (ii)  the  consummation  of  the  transactions  contemplated  hereby,  have  been  duly
taken.

(c)

Assuming  the  due  authorization,  execution  and  delivery  by  the  other  Party,  this
Agreement constitutes a legally valid and binding obligation of such Party, enforceable against it in
accordance with its terms (except in all cases as such enforceability may be limited by applicable
bankruptcy,  insolvency,  reorganization,  moratorium,  or  similar  Applicable  Laws  affecting  the
enforcement of creditors’ rights generally and except that the availability of the equitable remedy
of specific performance or injunctive relief is subject to the discretion of the court or other tribunal
before which any proceeding may be brought).

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(d)

There  is  no  contractual  restriction  or  obligation  binding  on  such  Party  or  its
Affiliates which would be materially contravened by execution and delivery of this Agreement or
by the performance of its terms.  There are no governmental filings or consents required of such
Party  or  its  Affiliates  necessary  for  the  consummation  of  this  Agreement  and  the  transactions
contemplated hereby.

(e)

Such Party is not debarred,  and  such  Party  in  relation  to  the  Product  is  not  using,
has  not  used,  and  will  not  use  in  any  capacity  the  services  of  any  Person  debarred,  in  each  case
under Subsection 306(a) of the Generic Drug Enforcement Act of 1992, or comparable laws, rules
and regulations in any other Country in the Territory.

13.2 Additional  Representations  and  Warranties  of  Applied.    Applied  hereby  further

represents and warrants to Advanz as of the Effective Date, that:

(a)

Exhibit B contains a complete and correct list as of the Effective Date of all Patents

Rights Controlled by Applied in the Field and Territory covering the Compound or any Product.

(b)

Applied owns or has valid rights to use and sublicense, the Applied Patent Rights in
existence  on  the  Effective  Date,  and  the  Applied  Patent  Rights  set  forth  on  Exhibit B  are  in  full
force and effect and have been maintained to date.

(c)

To  the  knowledge  of  Applied,  there  is  no  pending  action  or  claim  threatened  in
writing by a Third Party challenging the ownership, validity or scope of any Applied Patent Rights
in existence as of the Effective Date.

(d)

To the knowledge of Applied, subject to having undertaken a reasonable freedom-
to-operate investigation, the Manufacture, Commercialization or other Exploitation of Product as
contemplated under this Agreement will not infringe or otherwise violate any Patent of any Third
Party that exists on the Effective Date or, if and when issued, any Valid Claim within any Third
Party Patent Application published before the Effective Date.

(e)

To the knowledge of Applied, Applied has complied in all material respects with all

Applicable Laws, with respect to the Development of Product.

(f)

Applied  has  not  received  any  Form  483  observations,  warning  letters  or  other
communications  from  a  Regulatory  Authority  which  would  reasonably  be  expected  to  adversely
impact the Manufacture or the marketing of Product in any material respect.

13.3 Additional  Representation  and  Warranty  of  Advanz.    Advanz  hereby  further
represents and warrants to Applied as of the Effective Date to the knowledge of Advanz, neither
Advanz  nor  any  of  its  Affiliates  (a)  is  engaged  in  the  Development  or  Commercialization  of  a
Competing Product nor (b) has in effect a written plan to Develop or Commercialize a Competing
Product.

13.4

Solvency  Representation  and  Warranty  of  Applied.    Applied  hereby  further
represents and warrants to Advanz that, as of the Effective Date, Applied does not intend to incur,
and  is  not  presently  incurring,  debts  and  liabilities  that  will  be  beyond  its  ability  to  pay  as  such
debts and liabilities mature, to the extent known, probable and estimable.

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13.5 Certain Covenants of the Parties.

(a)

Each Party shall conduct, and shall cause its Affiliates to conduct, all its activities
contemplated  under  this  Agreement  in  accordance  with  all  Applicable  Laws  of  the  Country  in
which such activities are conducted.

(b)

Each Party shall provide written notice to the other Party in the event that it suffers
an insolvency related event of the type set out in Section 16.1(b) including the name and contact
details  of  any  receiver,  trustee,  assignee  for  the  benefit  of  creditors,  custodian  or  other  similar
official.

(c)

Advanz shall undertake any actions which it is required to take under any applicable
Antitrust  Laws  in  the  Territory  in  connection  with  transactions  contemplated  hereunder,  or  the
rights granted to, or obligations of, either Party hereunder, whether at the Effective Date or at any
time during the Term.

13.6 Disclaimer  of  Warranty.    EXCEPT  AS  OTHERWISE  EXPRESSLY  STATED  IN
THIS  AGREEMENT,  NEITHER  PARTY  MAKES  ANY,  AND  EACH  PARTY  DISCLAIMS
ALL,  REPRESENTATIONS  AND  WARRANTIES  OF  ANY  KIND,  EXPRESS  OR  IMPLIED,
WITH  RESPECT  TO  THE  COMPOUND,  DRUG  SUBSTANCE,  PRODUCT,  SUCH  PARTY’S
TECHNOLOGY  OR  PATENT  RIGHTS,  OR  ANY  OTHER  MATTER,  INCLUDING
WARRANTIES  OF  MERCHANTABILITY,  CONDITION,  QUALITY,  PERFORMANCE,
FITNESS  FOR  A  PARTICULAR  PURPOSE,  AND  NONINFRINGEMENT  OF  THE
INTELLECTUAL PROPERTY RIGHTS OF THIRD PARTIES.

SECTION 14.NON-COMPETITION

14.1 Advanz Non-Compete.  From the Effective Date and throughout the Term, neither
Advanz  nor  any  of  its  Affiliates  (including  through  any  acquisition)  shall,  directly  or  indirectly,
alone  or  in  collaboration  with  any  Third  Party  Commercialize,  in  any  Country,  any  Competing
Product.

SECTION 15.TERM

15.1

Term.  This Agreement shall be effective as of the Effective Date and shall remain

in effect until terminated pursuant to Section 16 (the “Term”).

SECTION 16.TERMINATION

16.1

Termination Rights.  This Agreement may be terminated as follows:

(a)

Material  Breach.    Either  Party  may  terminate  this  Agreement  at  any  time  upon
written notice to the other Party if the other Party is in material default or breach of this Agreement
and  such  material  default  or  breach  is  not  cured  within  (i)  sixty  (60)  days  after  written  notice
thereof is delivered to the defaulting or breaching Party, or (ii) in the case of a breach that cannot
be  cured  within  sixty  (60)  days,  within  a  reasonable  period  not  exceeding  ninety  (90)  days  after
written  notice  thereof  is  delivered  to  the  defaulting  or  breaching  Party,  so  long  as  the  breaching
Party in each case is making a good faith effort to cure such default.  For the avoidance of doubt,

18

the Parties agree that any Supply Shortage shall not constitute a material breach of this Agreement
and  shall  not  entitle  Advanz  to  terminate  this  Agreement,  and  such  Supply  Shortage  shall  be
addressed  in  accordance  with  Sections 8.12 to 8.14  inclusive.    Termination  shall  not  be  the  sole
remedy  for  material  breach  of  this  Agreement,  and  a  Party  may  choose  to  continue  to  perform
hereunder  and,  in  response  to  any  material  breach,  may  bring  a  claim  for  damages  and  other
available  remedies  under  this  Agreement,  including  in  accordance  with  Section  18.3,  where
applicable, such as a claim for injunctive relief, and bringing such a claim in good faith shall not
constitute a breach of this Agreement.

(b)

Insolvency.

Either  Party  may  terminate  this  Agreement  upon  written  notice  to  the  other  Party,  if  the
other  Party  files,  or  has  filed  against  it,  a  petition  for  voluntary  or  involuntary  bankruptcy  or
pursuant to any other insolvency law seeking to adjudicate it as bankrupt or insolvent, or seeking
dissolution, liquidation, winding up, reorganization, arrangement, adjustment, protection, relief of
debtors, an assignment for the benefit of creditors, or seeking the entry of an order for relief or the
appointment of a receiver, trustee, assignee for the benefit of creditors, custodian or other similar
official for any such Person or for any substantial part of its property, and, if such proceeding is
commenced  involuntarily,  either  such  proceeding  shall  remain  undismissed  or  unstayed  for  a
period of sixty (60) days.  The voluntary commencement of any of the foregoing proceedings by a
Party shall result in an immediate right to terminate by the other Party.

(c)

Patent  Challenge.    Applied  may  terminate  this  Agreement  as  provided  in  and  in

accordance with Section 2.6(b).

(d)

Approval  Failure;  Material  Safety  Issue.    In  the  event  that  the  Product  does  not
receive Marketing Authorization for use in a Licensed Indication in any Country in the Territory
by [***], then Advanz at its sole discretion may terminate this Agreement upon thirty (30) days’
notice; provided that such notice is delivered to Applied by [***].  In the event of a Material Safety
Issue,  the  Parties  shall  confer  and  use  Commercially  Reasonable  Efforts  to  ascertain  the
appropriate  course  of  action;  provided  that  where  no  other  option  or  recourse  is  reasonably
available  (including  recall  of  the  Product)  either  Party  may  terminate  this  Agreement  upon  the
occurrence of a Material Safety Issue in its entirety upon ten (10) days prior written notice to the
other Party.

(e)

Failure  to  Commercialize.    Without  limiting  its  rights  under  Section  16.1(a)  and
subject at all times to Applied’s material compliance with its obligations to fulfil Purchase Orders
in  accordance  with  Section  8.2,  such  that  Advanz  has  sufficient  Product  to  Commercialize  in
accordance with the Commercialization Plan for the duration of the relevant period:

(i)

Subject  to  the  provisos  set  out  in  Section  7.1,  Applied  may  terminate  this
Agreement  in  its  entirety,  or  if  otherwise  as  agreed  by  the  Parties  (which
may  include  termination  on  a  Country  by  Country  basis),  upon  at  least
ninety (90) days’ written notice to Advanz, if Advanz does not either:

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(A)

(B)

(C)

Launch the Product for each Licensed Indication in Germany within
[***] after the grant of any Marketing Authorization for the Product
for such Licensed Indication(s) by EMA; or

from 

Launch  the  Product  for  each  Licensed  Indication  in  France  within
[***] 
securing  Price  Approval  and/or  Third  Party
reimbursement approval (as applicable) whether pursuant to an Early
Access Program or otherwise; or

Launch  the  Product  for  each  Licensed  Indication  in  each  of  Italy,
Spain  and  the  United  Kingdom  within  [***]  after  the  grant  of  a
Marketing  Authorization  for 
the  Product  for  such  Licensed
Indication by EMA or the MHRA (whichever is the later); [***];

provided, however, that in each case, that Advanz shall have sixty (60) days from receipt of such
notice to Launch the Product for use in such Licensed Indication in such Country(ies).

(ii)

Termination for failure to achieve Minimum Sales/Quantities: Applied may
terminate  this  Agreement  in  its  entirety,  upon  ninety  (90)  days’  written
notice  to  Advanz,  if  Advanz  has  not  achieved  at  least  [***]  in  cumulative
Net Sales by the later of:

(A)

[***]

(B)

the date on which Advanz has [***],

provided  in  (B)  that  Advanz  has  submitted  the  Product  for,  and  used
Commercially Reasonable Efforts to prosecute Price Approval in each of the
Major  Markets  for  Galactosemia  within  [***]  and  provided,  however,  that
Advanz shall have sixty (60) days from receipt of such notice to cure such
failure  (where  any  cure  may  include  payment  of  any  shortfall  in  Royalties
on Net Sales below [***].

(f)

Gross negligence and willful misconduct. Advanz may terminate this Agreement in
the event of Applied’s gross negligence and/or willful misconduct of any of its obligations under
this Agreement and such gross negligence and/or willful misconduct is not cured within sixty (60)
days  after  written  notice  thereof  is  delivered  to  Applied.   As  used  in  this  Section  16.1(f),  “gross
negligence” means a lack of care that demonstrates reckless disregard for a party’s obligations and
a lack of consideration of the consequences or potential damage its actions may cause to the other
party; and “willful misconduct” means that a Person intentionally acts or fails to act knowing that
their conduct will probably result in harm or damage.

16.2 Continuing  and  Accrued  Obligations.    After  notice  of  termination  is  given  and,
subject to the further provisions of this Section 16.2, prior to the effective date of termination, this
Agreement, including all payment obligations hereunder, shall continue in full force and effect, and
the Parties shall continue to carry out and perform their respective Development, Manufacturing,
Commercialization and other Exploitation activities in accordance with this Agreement through the
effective date of termination.  Without limitation of the foregoing,

18

termination of this Agreement for any reason (a) shall be without prejudice to and shall not impair
or  limit  in  any  manner  (i)  Applied’s  right  to  receive  payment  from  Advanz  of  Royalties  or
Commercial  Event  Milestone  Payments  in  respect  of  sales  of  Product  in  the  Territory  occurring
prior to the effective date of such termination, whether or not the due date for such payment is after
such  effective  date  of  termination;  (ii) Applied’s  right  to  receive  the  applicable  Event  Milestone
Payment in respect of any Event Milestone which occurs prior to the effective date of termination,
whether  or  not  the  due  date  for  such  payment  is  after  such  effective  date  of  termination,
(iii) Applied’s right to receive payment from Advanz in accordance with this Agreement for any
Bulk Product ordered by Advanz and delivered pursuant to this Agreement prior to the effective
date of such termination, whether or not the due date for such payment is after such effective date
of termination, provided that such Bulk Product is Manufactured and delivered in accordance with
the  terms  of  this  Agreement;  and  (iv)  any  remedies  that  either  Party  may  have  and  (b)  shall  not
release  a  Party  hereto  from  any  indebtedness,  liability,  payment  or  other  obligation  incurred
hereunder  (including  liability  for  breach  of  this  Agreement)  by  such  Party  prior  to  the  effective
date of termination.

16.3

Effects of Termination.

(a)

Upon termination of this Agreement by Advanz under Section 16.1(f):

(i)

(ii)

(iii)

all  licenses  granted  to  Advanz  by  Applied  under  this  Agreement  shall  be
retained by Advanz and shall survive termination of this Agreement on the
same terms on which they were granted; provided that such licenses under
Applied  Technology,  Applied  Patents  and  Licensed  Trademarks  shall  be
expanded  to  enable  the  continuation  or  commencement  by  Advanz  of  any
activities  either  undertaken  by  Applied  or  any  other  Person  on  Applied’s
behalf  or  required  to  be  undertaken  by  Applied  or  any  other  Person  on
Applied’s behalf, in each case, relating to or associated with the Exploitation
of the Product for use in the Field in the Territory (including in relation to
Development  and  Manufacture  of  the  Product)  in  accordance  with  this
Agreement;

ownership  of  any  Marketing  Authorization  Application  or  Marketing
Authorization  relating  to  the  Compound  or  the  Product  which  is  held  by
Advanz, its Affiliates or designees, shall continue to be held by such entity;

to  the  extent  permitted  by  such  Third  Party,  (x)  all  Third  Party  contract
manufacturing/supply  agreement(s)  and  any  contract  development
agreements,  to  the  extent  applicable  to  the  Product  in  the  Field  in  the
Territory,  shall  be  assigned  to  Advanz  by  Applied  (unless  Advanz  notifies
Applied  otherwise  in  writing)  and  (y)  Applied  shall  ensure  that  (and  shall
procure the same to the extent Applied has not entered into such agreements
as of the Effective Date) it has adequate arrangements to give full effect to
such assignments.  Applied shall facilitate the assignment process (including
making any introductions) and shall not do anything to prejudice Advanz’s
rights under such licenses or agreements without the prior consent

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(iv)

(v)

of  Advanz  (such  consent  not  to  be  unreasonably  withheld,  conditioned  or
delayed);

if it has not already done so in accordance with the terms hereunder, Advanz
may  notify  Applied  that  it  wishes  to  use  its  Secondary  Source  Site,  or  if
Step-In  is  otherwise  triggered,  in  each  case,  Applied  shall  provide  all
reasonable  assistance  to  Advanz  to  effect  the  transfer  of  Manufacturing  of
Bulk Product;

Applied shall provide to Advanz copies of any reports or other materials in
its possession or control forming part of the Applied Technology including
those  required  for  any  Regulatory  Filing  related  to  the  Product  (e.g.
Dossiers, Required Existing Studies, Required Post-MA Studies and, subject
to  Section  4.3(d),  Other  Post  Approval  Studies  conducted  by  Applied)  to
enable Advanz to continue to Develop, Manufacture and Commercialize the
Product in the Field in the Territory;

(vi)

Advanz  shall  retain  all  materials  in  its  possession  relating  to  the  Product
and/or  which  it  requires  to  continue  to  Develop,  Manufacture  and
Commercialize the Product in the Field in the Territory, including:

(A)

(B)

(C)

(D)

all  Regulatory  Filings,  Regulatory  Approvals,  Price  Approvals,
contracts  and  other  agreements  relating  to  Pricing  and  Market
Access  Activities  in  Advanz’s  possession  or  control  to  the  extent
related to the Product;

all reports, records, information (including drug master files, if any),
regulatory  correspondence,  correspondence  with  respect  to  Pricing
and  Market  Access  Activities,  and  other  materials  in  Advanz’s
possession or control to the extent relating to the Product in the Field
in the Territory;

all materials bearing any Licensed Trademarks; and

all Applied Confidential Information (which shall remain subject to
Section 12);

(vii) without  limiting    Section  8.15,  Sections  9.2  and  9.3  shall  survive
notwithstanding  references  to  the  duration  of  the  Term,  and  Advanz  shall
remain liable to pay any Royalties and any Event Milestone Payments to the
extent due and payable;

(viii) Applied shall transfer to Advanz all inventory of the Bulk Product which is
subject to a Purchase Order and has not yet been provided, and Advanz shall
be entitled to sell all of its inventory of the Bulk Product.  For the avoidance
of doubt, Advanz’s remedies set out in Sections 8.7(b) and (d) shall apply to
any such inventory;

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(ix)

(x)

(xi)

Applied  shall,  upon  request  of  Advanz,  return  or  destroy  all  Advanz
Confidential  Information  disclosed  to  it  pursuant  to  this  Agreement,
including  all  copies  and  extracts  of  documents,  as  promptly  as  practicable
following  receipt  of  such  request,  except  that  copies  may  be  kept  for  the
purpose of complying with continuing obligations under this Agreement to
the extent and for so long as necessary to perform its obligations or exercise
its  rights  under  this  Section  16.3(a).    Notwithstanding  the  foregoing,
Applied  also  shall  be  permitted  to  retain  such  additional  copies  of  or  any
computer  records  or  files  containing  Advanz  Confidential  Information  (A)
to  the  extent  necessary  to  comply  with  Applicable  Laws  or  (B)  that  have
been  created  solely  by  Applied’s  automatic  archiving  and  back-up
procedures,  to  the  extent  created  and  retained  in  a  manner  consistent  with
Applied’s standard archiving and back-up procedures, but not for any other
use or purpose.  For the avoidance of doubt, any Confidential Information of
Advanz  retained  by  Applied  in  accordance  with  this  Section  16.3(a)  shall
remain  Confidential  Information  of  the  disclosing  Party  and  subject  to
Section 12;

for  clarity,  Advanz’s  termination  of  the  Agreement  under  Section  16.1(f)
shall trigger its Step-In rights under Section 8.14(a); and

the  following  Sections  of  this  Agreement  shall  survive  such  termination
under Section 16.1(f): Sections 2.1, 2.2, 2.3, 2.4, 2.6, 2.7, 4.3(c) and (d), 5.4
(as  required  to  comply  with  Applicable  Laws),  7.3,  7.4,  8.14,  8.15  (as
required to give effect to this Section 16.3(a)), 9, 10, 11,  12,  13.5(a),  13.6,
16.1(b), 16.1(c), 16.1(d), 16.1(e), 16.2,  16.3(b),  17  (including  Section  17.5
notwithstanding  references  to  the  duration  of  the  Term  therein),  18,  19.2
through  19.16  (inclusive),  Exhibit  H  (to  the  extent  required  by  the  Third
Party  Licenses)  and  any  other  Exhibits  to  the  extent  required  for
interpretation purposes.

(b)

Upon termination of this Agreement (except by Advanz under Section 16.1(f)):

(i)

Advanz  shall  (or,  in  each  case,  shall  cause  its  designee,  if  applicable,  to),
promptly  after  such  termination,  supply  to  Applied  or  its  designee  the
following  materials;  provided  that  such  materials  shall  be  supplied  in  the
form and format in which such materials are maintained by Advanz in the
ordinary course of business (provided that Advanz shall use Commercially
Reasonable Efforts to provide such materials in a form and format useable
by Applied):

(A)

all  Regulatory  Filings 
(including  Marketing  Authorizations),
Regulatory  Approvals,  Price  Approvals,  contracts  and  other
agreements  in  Advanz’s  or,  if  applicable,  its  designee’s,  possession
or control to the extent related to a Product;

18

(B)

(C)

(D)

all reports, records, information (including drug master files, if any),
regulatory correspondence and data, correspondence with respect to
Pricing  and  Market  Access  Activities,  and  other  materials  in
Advanz’s or, if applicable, its designee’s, possession or control to the
extent relating to a Product;

all materials bearing any Licensed Trademarks;

assign to Applied any and all right, title or interest of Advanz in any
Trademarks actually used in commerce by Advanz or its Affiliates in
connection  with  a  Product  (including  in  any  Licensed  Trademarks
and  any  goodwill  associated  therewith),  excluding,  for  clarity,  the
corporate  or  trade  name  or  logo  of  Advanz  or  its  Affiliates.    In
furtherance of the foregoing Advanz shall execute an assignment of
any  such  Trademarks  in  favor  of  Applied  or  an  Applied  Affiliate
identified  by  Applied  and  Applied  (or  such  Applied  Affiliate
designee)  shall  be  responsible  for  recording  such  assignment  with
the  appropriate  governmental  trademark  authorities;  provided  that
in  facilitating  such  assignment  and
Advanz  shall  cooperate 
recordation by timely executing all necessary documents provided to
it by Applied.

(ii)

Advanz hereby does, on behalf of itself and any of its applicable designees,
(and shall) assign to Applied, or an Applied Affiliate identified by Applied,
all of Advanz’s or its Affiliates’ or designee’s (as applicable) right, title and
interest  in  and  to  the  materials  transferred  or  delivered  or  deliverable  by
Advanz  pursuant  to  Section  16.3(b)(i),  to  the  extent  Advanz  or  any  of  its
Affiliates  or  designees  control  such  materials,  which  assignment  shall
include, for the avoidance of doubt, transfer of all physical items relating to
Marketing Authorizations and Marketing Authorization Applications for the
Product  in  Advanz’s  or  any  of  its  Affiliate’s  or  designee’s  name  and
commencement  of  the  transfer  process  with  the  applicable  Regulatory
Authorities;

(iii)

Advanz  hereby  does  (and  shall)  assign  to  Applied  any  applicable
sublicenses  to  the  extent  related  to  the  Product  and/or  Third  Party
agreements,  with  respect  to  significant  services  to  be  performed  by  Third
Parties  to  the  extent  related  to  the  Product,  unless  Applied  has  advised
Advanz that it will not require such assignment.

(iv) Without  limitation  of  the  generality  of  the  foregoing,  upon  Applied’s
request, the Parties shall use diligent efforts to complete the transition of the
Commercialization  of  the  Product,  as  well  as  Advanz’s  responsibilities
hereunder  with  respect  thereto  (including  pharmacovigilance  and  Pricing
and Market Access Activities) and at Applied’s election and request, and to
extent reasonably possible and legally permissible, transfer and sale of some
or all Product inventory and Bulk Product then in possession or control of

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(v)

Advanz, its Affiliates or sublicensees at cost to Applied (or its sublicensee
or  Third  Party  designee)  as  soon  as  is  reasonably  possible,  in  a  low  risk,
orderly fashion.

Each of Advanz and Applied shall, upon request of the other Party, return or
destroy  all  Applied  Confidential  Information  and  Advanz  Confidential
Information disclosed to it pursuant to this Agreement, including all copies
and  extracts  of  documents,  as  promptly  as  practicable  following  receipt  of
such  request,  except  that  one  (1)  copy  may  be  kept  for  the  purpose  of
complying  with  continuing  obligations  under  this  Agreement  including
relating to termination (e.g., under Section 16.1(b)(iv)) to the extent and for
so  long  as  necessary  to  perform  its  obligations  or  exercise  its  rights  under
this Section 16.3(b).    Notwithstanding  the  foregoing,  such  other  Party  also
shall  be  permitted  to  retain  such  additional  copies  of  or  any  computer
records  or  files  containing  such  Confidential  Information  (A)  to  the  extent
necessary  to  comply  with  Applicable  Laws  or  (B)  that  have  been  created
solely  by  such  Party’s  automatic  archiving  and  back-up  procedures,  to  the
extent  created  and  retained  in  a  manner  consistent  with  such  other  Party’s
standard  archiving  and  back-up  procedures,  but  not  for  any  other  use  or
purpose.    For  the  avoidance  of  doubt,  any  Confidential  Information  of  the
disclosing  Party  retained  by  the  receiving  Party  in  accordance  with  this
Section  16.3(b)  shall  remain  Confidential  Information  of  the  disclosing
Party and subject to Section 12.

SECTION 17.INDEMNIFICATION, INSURANCE AND LIABILITY

17.1

Indemnification  by  Advanz.    Subject  to  Sections  17.3  and  17.4,  Advanz  shall
indemnify,  defend  and  hold  Applied,  its  Affiliates,  and  their  respective  directors,  officers,
employees,  consultants,  contractors,  sublicensees  and  agents  (collectively, 
the  “Applied
Indemnitees”) harmless from and against any and all claims, suits, proceedings or causes of action
(“Claims”) brought by a Third Party against such Applied Indemnitee, including any damages or
other  amounts  payable  to  such  Third  Party  and  reasonable  attorneys’  fees  and  costs  of  litigation
(collectively, “Damages”), in each case to the extent resulting from or based on: (a) any Taxes for
which  Advanz  is  responsible  pursuant  to  this  Agreement;  b)  Advanz’s  breach  of  this  Agreement
(including its representations, warranties and obligations herein); (c) the determination of Advanz
not  to  initiate  an  Advanz  Recall  in  the  exercise  of  its  discretion  under  Section  5.5(c);  or  (d)  the
gross  negligence  or  willful  misconduct  of,  or  violation  of  Applicable  Laws  by,  Advanz,  its
Affiliates  or  its  Sublicensees,  or  their  respective  employees,  contractors  or  agents  in  the
performance of this Agreement, except to the extent such Damages result from any of Applied’s
acts or omissions that are not in accordance with the Agreement.

17.2

Indemnification  by  Applied.    Subject  to  Sections  17.3  and  17.4,  Applied  shall
indemnify,  defend  and  hold  Advanz,  its  Affiliates,  and  their  respective  directors,  officers,
employees,  consultants,  contractors,  sublicensees  and  agents  (collectively, 
the  “Advanz
Indemnitees”) harmless from and against any and all Claims brought by a Third Party against such
Advanz Indemnitee, including any Damages, in each case to the extent resulting from or based on:
(a) Applied’s breach of this Agreement (including its representations, warranties and obligations

18

herein);  (b)  the  determination  of  Applied  not  to  initiate  an  Applied  Recall  in  the  exercise  of  its
discretion under Section 5.5(c); or (c) the gross negligence or willful misconduct of, or violation of
Applicable  Laws  by,  Applied,  its  Affiliates  or  sublicensees,  or  their  respective  employees,
contractors  or  agents  in  the  performance  of  this  Agreement,  except  to  the  extent  such  Damages
result from any of Advanz’s acts or omissions that are not in accordance with this Agreement.

17.3

Indemnification of Product Liability Claims.

(a)

Notwithstanding  any  other  provision  of  this  Agreement,  this  Section  17.3  shall
govern the allocation of liability with respect to any Third Party product liability Claim, including
Claims of property injury, bodily injury or deaths related to the Product in the Territory (a “Third
Party Product Claim”).

(b)

Subject  to  Section  17.4,  Applied  shall  indemnify,  defend  and  hold  harmless  the
Advanz  Indemnitees  from  and  against  any  and  all  Damages  which  an  Advanz  Indemnitee  may
incur or suffer arising out of any Third Party Product Claim to the extent caused by, resulting or
arising from its Development activities (whether prior to or during the Term) or Manufacture of the
Product  (including  any  defect  in  the  Manufacturing  of  the  Bulk  Product  supplied  by  Applied  to
Advanz hereunder).

(c)

Subject to Section 17.4 and except to the extent Applied is obligated to indemnify
the  Advanz  Indemnitees  in  respect  of  such  Damages  pursuant  to  Section 17.3(b)  above,  Advanz
shall indemnify, defend and hold harmless the Applied Indemnitees from and against any and all
Damages arising out of any Third Party Product Claims to the extent caused by, resulting or arising
from its Development activities, its Secondary Packaging and Release activity and any other Step-
In Rights or Secondary Source Site or other Manufacture or Commercialization, in each case of the
Product in the Territory.

(d)

The indemnity in this Section 17.3 shall include defects stipulated in Article 1 of the

EU Product Liability Directive [85/374/EEC].

17.4 Defense Procedures; Procedures for Third Party Claims.

(a)

For purposes of this Agreement, “Third Party Claim” means a Claim asserted by a
Third  Party  (in  no  event  to  include  any  Affiliate  of  either  Party)  against  a  Party  or  any  of  its
Affiliates,  or  any  of  their  respective  directors,  officers,  employees,  consultants,  contractors,
sublicensees and agents.  In the event a Third Party Claim is asserted with respect to any matter for
which  a  Party  or  any  of  its  Affiliates,  or  any  of  their  respective  directors,  officers,  employees,
consultants,  contractors,  sublicensees  and  agents  (the  “Indemnified  Party”)  is  entitled  to
indemnification  hereunder,  then  the  Indemnified  Party  shall  promptly  notify  in  writing  the  Party
obligated  to  indemnify  the  Indemnified  Party  hereunder  (the  “Indemnifying  Party”)  thereof;
provided, however, that no delay on the part of the Indemnified Party in notifying the Indemnifying
Party shall relieve the Indemnifying Party from any obligation hereunder unless (and then only to
the extent that) the Indemnifying Party is prejudiced thereby.

(b)

The Indemnifying Party shall assume direction and control of the defense, litigation,
settlement,  appeal  or  other  disposition  of  the  Third  Party  Claim  (including  the  right  to  settle  the
Claim solely for monetary consideration) with counsel selected by the Indemnifying

18

Party  and  reasonably  acceptable  to  the  Indemnified  Party.    The  Indemnified  Party  shall  provide
reasonable  assistance  to  the  Indemnifying  Party  in  relation  to  such  Third  Party  Claim  and  shall
have the right to join in (including the right to conduct discovery, interview and examine witnesses
and  participate in all  settlement  conferences),  but  not  control,  at  its  own  expense, the defense of
any  Third  Party  Claim  that  the  Indemnifying  Party  is  defending  as  provided  in  this  Agreement.
 Notwithstanding anything to the contrary contained herein, an Indemnified Party shall be entitled
to assume the defense of any Third Party Claim with respect to the Indemnified Party, upon written
notice to the Indemnifying Party, in which case the Indemnifying Party shall be relieved of liability
under Section 17.1 or 17.2, as applicable, solely for such Third Party Claim and related Damages.

(c)

Neither  Party  will  enter  into  any  settlement  of  any  suit  involving  Products  that
materially affects the other Party’s rights or obligations with respect to the Product (including any
settlement limiting the scope, validity or enforceability of the other Party’s Intellectual Property)
without the other Party’s prior written consent (which consent shall not be unreasonably withheld,
delayed or conditioned).  Without limiting the foregoing, the Indemnifying Party shall not, without
the  prior  written  consent  of  the  Indemnified  Party  (which  consent  shall  not  be  unreasonably
withheld, delayed or conditioned), effect any settlement of any pending or threatened litigation in
which  the  Indemnified  Party  has  sought  indemnification  hereunder  by  the  Indemnifying  Party,
unless such settlement involves solely monetary damages and includes an unconditional release of
the Indemnified Party from all liability on Claims that are the subject matter of such litigation.

17.5

Insurance.    During  the  Term  and  for  three  (3)  years  thereafter,  each  Party  shall
maintain  public  liability  insurance  coverage  up  to  Ten  Million  Euros  (€10,000,000).    Each  Party
shall provide a certificate of insurance evidencing such coverage to the other Party upon request
and shall reasonably cooperate with the other Party in order to maximize any insurance recoveries.

17.6 Disclaimer of Liability for Consequential Damages.

(a)

SUBJECT TO SECTION 17.6(b):

(i)

(ii)

EITHER  PARTY  SHALL  BE  ENTITLED  TO  CLAIM  DAMAGES  FOR
DIRECT  LOSS  OF  PROFITS  UP  TO  A  LIMIT  OF  [***]  PER
CALENDAR YEAR.

IN NO EVENT SHALL EITHER PARTY OR ANY OF ITS RESPECTIVE
AFFILIATES  BE  LIABLE  UNDER  OR  IN  CONNECTION  WITH  THIS
AGREEMENT  FOR  ANY  LOSS  OF  REVENUES  OR  CONTRACTS,
BUSINESS  INTERRUPTION,  INDIRECT  LOSS  OF  PROFITS  OR  ANY
OTHER  INDIRECT,  SPECIAL,  INCIDENTAL  OR  CONSEQUENTIAL
DAMAGES,  WHETHER  IN  CONTRACT,  UNDER  A  WARRANTY,
TORT 
(INCLUDING  NEGLIGENCE),  UNDER  STATUTE  OR
OTHERWISE.

THE  FOREGOING  SENTENCE  SHALL  NOT  LIMIT  THE  OBLIGATIONS  OF
EITHER PARTY TO INDEMNIFY THE OTHER PARTY FROM AND AGAINST
THIRD  PARTY  CLAIMS  UNDER  SECTION  17.3  OR  LIABILITIES
RESULTING FROM A BREACH OF THE CONFIDENTIALITY

18

OBLIGATIONS UNDER SECTION 12 ABOVE, OR ANY LIABILITY ARISING
OUT  OF  ANY  INFRINGEMENT  OR  OTHER  VIOLATION  OF  THE  APPLIED
PATENT  RIGHTS,  THE  APPLIED  TECHNOLOGY  OR  THE  LICENSED
TRADEMARKS AS A CONSEQUENCE OF THEIR USE BY ADVANZ OR ITS
AFFILIATES OTHER THAN IN ACCORDANCE WITH THIS AGREEMENT.

(b)

Neither Party excludes nor limits any liability for:

(i)

death  or  personal  injury  to  the  extent  caused  by  the  negligence  or  willful
default of a Party or its employees;

(ii)

fraud or fraudulent misrepresentation;

(iii)

(iv)

any  breach  of  any  obligations  implied  by  section  12  of  the  Sale  of  Goods
Act 1979 or section 2 of the Supply of Goods and Services Act 1982;

any other liability to the extent the same cannot be excluded or limited by
Applicable Laws; or

(v)

its payment obligations under this Agreement.

SECTION 18.GOVERNING LAW AND JURISDICTION

18.1 Governing Law.  This Agreement and any non-contractual obligations arising out of
or  in  connection  with  it  shall  be  governed  by  and  construed  in  accordance  with  the  Laws  of
England and Wales.  The provisions of the U.N. Convention on Contracts for the International Sale
of Goods shall not apply to this Agreement.

18.2 U.S. Bankruptcy Matters.  Notwithstanding anything else to the contrary herein, this
Section  18.2  shall  apply  in  the  event  of  the  commencement  of  a  voluntary  or  involuntary
bankruptcy proceeding by or against Applied in the United States (provided that, in the case of an
involuntary bankruptcy proceeding, such proceeding has remained undismissed or unstayed for a
period of sixty (60) days).

(a)

All of the Intellectual Property which is subject to any of the licenses contained in
this  Agreement,  including  trademarks  (in  particular  the  Licensed  Trademarks)  and  all  of  the
Applied rights which Advanz requires to continue to Develop, Manufacture and/or Commercialize
the  Products  in  the  exercise  of  any  applicable  Step-In  Rights  or  as  set  out  in  Section 16.3(a)  (in
particular  continued  ownership  of  the  Marketing  Authorizations  and/or  Marketing  Authorization
Applications  relating  to  the  Product  in  the  Field  in  the  Territory)  (collectively,  the  “IP  Rights”),
constitute “intellectual property” pursuant to section 101(35A) of the U.S. Bankruptcy Code, and
any  rejection  of  this  Agreement,  including  the  license  provided  hereunder  and  any  associated
amendments,  amendments  and  restatements  or  modifications  hereto,  by  Applied  in  a  U.S.
bankruptcy proceeding shall be governed by the U.S. Bankruptcy Code, including section 365(n)
thereof.

18

(b)

The  IP  Rights  may  be  exercised  by  Advanz  in  accordance  with  any  applicable
license  terms  hereunder  notwithstanding  the  commencement  by  Applied  of  any  bankruptcy,
insolvency  or  similar  proceeding,  and  notwithstanding  the  imposition  of  the  automatic  stay
pursuant  to  section  362  of  the  U.S.  Bankruptcy  Code.    To  the  extent  necessary,  Applied  hereby
consents  to  relief  from  the  automatic  stay  pursuant  to  section  362  of  the  Bankruptcy  Code  to
permit Advanz to exercise the IP Rights in accordance with any applicable license terms hereunder
without further order of any court, and agrees to take all acts necessary to seek such consent and
the access needed to exercise such rights.

(c)

To  the  extent  Advanz  elects  to  retain  its  rights  under  section  365(n)(1)(B)  of  the
Bankruptcy  Code  following  any  rejection  of  this  Agreement,  including  the  license  provided
hereunder and any associated amendments, amendments and restatements or modifications hereto,
Advanz may exercise and shall be entitled to the benefits of the IP Rights in accordance with this
Agreement.

18.3

Jurisdiction  and  Dispute  Resolution  Process.   With  the  exception  of  those  matters
referred  for  resolution  by  independent  Third  Parties  under  Section  10.8,  by  independent
consultants  under  Section  8.7(c),  which  are  subject  to  equitable  relief  under  Section  19.15  or
subject  to  Section  18.3(c)(iv),  any  dispute,  controversy  or  claim  relating  to  any  contractual  and
non-contractual  obligations  arising  out  of  or  relating  to  this  Agreement,  or  the  interpretation  or
breach  thereof,  including  disputes  regarding  the  existence,  validity  or  termination  of  this
Agreement  or  the  scope  of  the  agreement  to  arbitrate  herein  (each,  a  “Dispute”),  shall  be
determined in accordance with the provisions of this Section 18.3:

(a)

If any Dispute arises, either Party may provide written notice of the Dispute to the
other  Party  and  request  negotiation  between  the  executive  officers  of  each  Party  (“Dispute
Notice”).   Within  fifteen  (15)  days  after  the  delivery  of  a  Dispute  Notice,  the  executive  officers
shall  confer  in  person  or  by  teleconference  to  attempt  to  settle  the  Dispute.   All  communication
between  such  executive  officers  shall  not  be  construed  as  an  admission  or  agreement  as  to  the
liability  of  any  Party,  nor  be  admitted  in  evidence  in  any  related  arbitration,  litigation,  or  other
adversary proceeding.

(b)

If,  within  [***]  after  the  delivery  of  a  Dispute  Notice,  the  Parties  are  unable  to
resolve the Dispute in writing, upon written notice by any Party to the other Party, such Dispute
shall be determined exclusively by final and binding arbitration administered by the London Court
of  International  Arbitration  in  accordance  with  its  International  Arbitration  Rules,  except  as
modified herein.

(c)

In any arbitration commenced pursuant to this Section 18.3:

(i)

There shall be three arbitrators, one of which shall be appointed by Applied
and  another  of  which  shall  be  appointed  by  Advanz,  in  each  case,  within
twenty  (20)  days  of  the  date  of  delivery  of  the  notice  of  arbitration.    The
third  arbitrator,  who  shall  serve  as  the  president  of  the  tribunal,  shall  be
jointly appointed by the two Party-appointed arbitrators within twenty (20)
days  of  the  date  of  appointment  of  the  second  arbitrator  to  be  appointed.
 Any arbitrator not timely appointed as provided herein shall be appointed,

18

(ii)

(iii)

(iv)

at the written request of any Party to the arbitration, by the London Court of
International Arbitration.

The  seat  of  arbitration  shall  be  London,  England.    The  language  of  the
arbitration  shall  be  English.   The  Parties  agree  that  the  award  rendered  by
the  arbitral  tribunal  shall  be  final  and  binding  and  enforceable  against  the
Parties  and  their  respective  assets  in  any  court  of  competent  jurisdiction.
  Unless  determined  otherwise  by  the  arbitral  tribunal,  each  Party  shall  pay
its  own  Costs  and  Expenses  in  connection  with  the  arbitration,  except  that
the  Parties  shall  pay  an  equal  share  of  all  Costs  and  Expenses  related  to
compensation of the arbitral tribunal and site and administrative fees.  The
arbitral tribunal shall not award any damages excluded by Section 17.6.

Any arbitration hereunder  shall  be  confidential,  and  neither  the  Parties  nor
their agents shall disclose to any Third Party not involved in the arbitration
the  existence  or  status  of  the  arbitration,  any  information  made  known  or
documents produced in the arbitration not otherwise available to them or in
the public domain, or any awards arising from the arbitration, except and to
the  extent  that  disclosure  is  required  by  Applicable  Laws  or  is  required  to
protect or pursue a legal right.

For any proceeding in aid of arbitration or to seek interim relief (such as an
injunction)  against  the  other  Party  to  protect  its  rights  and  interests,  or  to
enforce  the  obligations  of  the  other  Party,  each  Party  irrevocably  and
unconditionally consents and submits to the exclusive jurisdiction and venue
of  the  courts  of  England  and  Wales  located  in  London,  England  (“English
Courts”), and to the non-exclusive jurisdiction and venue of English Courts
for  any  action  to  enforce  any  arbitration  award  obtained  pursuant  to  this
Agreement.    In  any  such  action:  (i)  each  Party  irrevocably  waives,  to  the
fullest extent it may effectively do so, any objection, including any objection
to the laying of venue or based on the grounds of forum non conveniens or
any right of objection to jurisdiction on account of its place of incorporation
or domicile, which it may now or hereafter have to the bringing of any such
action  or  proceeding  in  the  English  Courts;  (ii)  each  Party  irrevocably
consents  to  service  of  process  in  the  manner  provided  for  notices  in  this
Agreement  or  in  any  other  manner  permitted  by  Applicable  Laws;  and
(iii)  each  Party  waives  any  right  to  trial  by  jury  in  any  court.
  Notwithstanding  the  foregoing,  the  arbitral  tribunal  also  shall  have  full
authority  to  grant  provisional  remedies  and  to  direct  the  Parties  to  request
that  any  court  modify  or  vacate  any  provisional,  temporary  or  preliminary
relief issued by a court hereunder.

(v)

Each Party shall continue to perform obligations hereunder, when any bona
fide Dispute is pending.

18.4

Third Party Licenses.  Notwithstanding anything to the contrary herein, with respect
to any Dispute arising out of or related to any Third Party License, such Dispute shall be governed

18

by and construed in accordance with the laws of the State of New York, without reference to or
reliance  upon  its  rules  regarding  conflicts  of  laws  and  shall  be  subject  to  the  dispute  resolution
provisions set forth in the applicable Third Party License.

SECTION 19.MISCELLANEOUS

19.1

Force Majeure.  Excluding payment obligations, neither Party hereto shall be liable
to the other Party for any Damages attributable to a default under or breach of this Agreement to
the  extent  resulting  from  war  (whether  declared  or  undeclared),  acts  of  God,  revolution,  acts  of
terror, fire, earthquake, flood, pestilence, riot, enactment or change of Applicable Laws (following
the  Effective  Date),  accident(s),  labor  trouble,  global  shortage  of  or  inability  to  obtain  material
equipment, supplies of the Product or any other cause beyond the reasonable control of such Party
and the effect of which could not have been mitigated by reasonable contingency planning (each, a
“Force Majeure Event”); provided that if such a cause occurs, then the Party affected will promptly
notify the other Party of the nature and likely result and duration (if known) of such cause and use
its  Commercially  Reasonable  Efforts  to  mitigate,  avoid  and/or  remove  such  causes  of
nonperformance  as  soon  as  is  reasonably  practicable.    Upon  termination  of  the  Force  Majeure
Event,  the  performance  of  any  suspended  obligation  or  duty  shall  promptly  recommence.    If  the
resulting default or event lasts for a period of longer than three (3) months, the Parties shall meet to
implement appropriate remedial measures; provided that, if the resulting default or event lasts for a
period of longer than six (6) months, the unaffected Party may terminate this Agreement.  Upon
the occurrence of a Force Majeure Event that lasts for a period of more than three (3) months, the
Parties  shall  arrange  a  meeting  between  Advanz’s  CEO  and/or  CFO  (or  equivalent  role)  and
Applied’s CEO and/or CFO (or equivalent role) to determine whether a continuity plan is required.
 In the event that Applied is the affected Party, Applied shall promptly submit to Advanz for its
approval (and once approved, implement), a continuity plan to deal with the consequences of the
Force Majeure Event as soon as reasonably practicable (the “FM Continuity Plan”).  If required by
Advanz, the FM Continuity Plan shall include rights for Advanz to exercise some or all of its right
to step-in under Section 8.14 following issue of a Step-In Notice to Applied.

19.2

Severability.  If and solely to the extent that any provision of this Agreement shall
be invalid or unenforceable, or shall render this entire Agreement to be unenforceable or invalid,
such offending provision shall be of no effect and shall not affect the enforceability or validity of
the  remainder  of  this  Agreement  or  any  of  its  provisions;  provided,  however,  that  the
unenforceable  or  invalid  provision  shall  be  replaced  in  a  manner  that  best  accomplishes  the
original  intentions  of  the  Parties,  by  agreement  of  the  Parties  or  by  a  court  of  competent
jurisdiction.

19.3 Waivers.  Any term or condition of this Agreement may be waived at any time by
the Party that is entitled to the benefit thereof, but no such waiver shall be effective unless set forth
in a written instrument duly executed by or on behalf of the Party waiving such term or condition.
 Neither the waiver by any Party of any term or condition of this Agreement nor the failure on the
part of any Party, in one or more instances, to enforce any of the provisions of this Agreement or to
exercise  any  right  or  privilege,  shall  be  deemed  or  construed  to  be  a  waiver  of  such  term  or
condition  for  any  similar  instance  in  the  future  or  of  any  subsequent  breach  hereof.   All  rights,
remedies,  undertakings,  obligations  and  agreements  contained  in  this  Agreement  shall  be
cumulative  and  none  of  them  shall  be  a  limitation  of  any  other  remedy,  right,  undertaking,
obligation or agreement.

18

19.4

Entire Agreements; Amendments.

(a)

This Agreement, the Quality Agreement and the Pharmacovigilance Agreement set
forth  the  entire  agreement  and  understanding  between  the  Parties  as  to  the  subject  matter  hereof
and supersedes and replaces any and all agreements, statements, arrangements or understandings,
verbal or written, made between Applied and Advanz before the Effective Date with respect to the
subject  matter  hereof,  including  the  Mutual  Confidentiality  Agreement  by  and  between  Advanz
Pharma  Services  (UK)  Limited  and  Applied  dated  July  5,  2022.  All  Confidential  Information
disclosed by either Party to the other Party prior to the Effective Date will be deemed, as of the
Effective Date, to have been disclosed pursuant to, and will be subject only to, this Agreement.

(b)

None of the terms of this Agreement shall be amended, supplemented or modified

except in writing signed by the Parties.

19.5

Survival.    The  provisions  of  Sections  2.7,  5.4  (as  required  to  comply  with
Applicable Laws), 7.4(c)  and  (h),  8.3, 10.8  (for  two  (2)  years),  12  (for  the  time  period  set  forth
therein), 13.6, 16.2, 16.3, 17.1 through 17.4 (inclusive), 17.5 (for three (3) years), 17.6, 18, 19.2
through 19.10 (inclusive), 19.12 and 19.14 through 19.15 (inclusive), and Exhibit H (to the extent
required by the Third Party Licenses), as well as (x) any other Sections or defined terms referred to
in  such  Sections  or  necessary  to  give  them  effect  and  (y)  any  other  provision  that  by  its  terms
expressly survives termination of this Agreement, shall survive termination of this Agreement and
remain  in  force  until  discharged  in  full.    Furthermore,  any  other  provisions  required  to  interpret
and  enforce  the  Parties’  rights  and  obligations  or  to  wind  up  their  outstanding  obligations  under
this  Agreement  shall  survive  to  the  extent  required.    For  clarity,  if  Section  16.3(a)  is  triggered,
survival shall be governed by Section 16.3(a)(xi).

19.6 Assignment; Binding Effect.

(a)

Neither  this  Agreement  nor  any  rights  or  obligations  of  either  Party  to  this
Agreement  may  be  assigned  or  otherwise  transferred  by  either  Party  without  the  consent  of  the
other Party; provided, however either Party may, without such consent, assign this Agreement, in
whole or in part to any of its respective Affiliates, but for only so long as such assignee remains an
Affiliate of such Party; provided that such assigning Party shall remain jointly and severally liable
with such Affiliate in respect of all obligations so assigned;

(b)

Advanz may assign this Agreement to a Third Party acquiror to all or substantially
all of the assets of Advanz, whether by merger or sale of all or substantially all of Advanz’s assets,
so long as such Third Party agrees in writing to be bound by the terms of this Agreement; and

(c)

Applied may assign this Agreement to a Third Party acquiror to all or substantially
all of the assets of Applied to which this Agreement relates, whether by merger or sale of line of
business or of all or substantially all of Applied’s assets to which this Agreement relates, so long as
such  Third  Party  agrees  in  writing  to  be  bound  by  the  terms  of  this  Agreement  and  the  relevant
Intellectual  Property  to  which  the  licenses  granted  to  Advanz  under  this  Agreement  relates,  are
transferred  to  such  assignee  (or  arrangements  shall  be  put  in  place  to  ensure  that  such  licenses
granted are not adversely affected in any way).

18

(d)

Notwithstanding  anything  to  the  contrary  herein,  nothing  herein  shall  prevent
Applied  or  its  Affiliates  from  engaging  in  any  merger,  consolidation,  reorganization,  sale  or
purchase of stock, or sale or purchase of assets, or undergoing any change of control, including in
each case with respect to any line of business, or prevent Applied or its Affiliates with respect to
any  royalty  or  milestone  sale,  collateralized  loan  or  other  financing.    For  clarity,  a  change  of
control of an entity does not constitute an assignment or transfer.

(e)

Any  purported  assignment  in  violation  of  this  Section  19.6  shall  be  void.    Any

permitted assignee shall assume all obligations of its assignor under this Agreement.

19.7

Independent Contractor.   The  relationship  between  Applied  and  Advanz  is  that  of
independent contractors.  Applied and Advanz are not joint venturers, partners, principal and agent,
employer and employee, and have no other relationship other than independent contracting parties.

19.8 Notices.    Each  communication  and  document  made  or  delivered  by  one  Party  to
another under this Agreement shall be made in the English language.  Subject to Section 3.1 and
Section 6, notices, consents, approvals, and requests required hereunder given by one Party to the
other hereunder shall be in writing and made by registered or certified air mail, express overnight
courier or delivered personally to the following addresses of the respective Parties:

If to Applied:

545 5th Avenue, Suite 1400
New York, NY 10017
Attn: Shoshana Shendelman, Chief Executive Officer

with a copy to:

Skadden, Arps, Slate, Meagher & Flom LLP
One Manhattan West
New York, NY 10001
Attn: Michael Schwartz

If to Advanz:

Capital House
1st Floor
85 King William Street
London
EC4N 7BL
Attn: Chief Corporate Development Officer

18

with a copy to:

Capital House
1st Floor
85 King William Street
London
EC4N 7BL

and by email to:

legalteam@advanzpharma.com
Attn: General Counsel

Notices hereunder shall be deemed to be effective (a) upon receipt if personally delivered; (b) on
the  tenth  (10th)  Business  Day  following  the  date  of  mailing  if  sent  by  registered  or  certified  air
mail; (c) on the second (2nd) Business Day following the date of transmission or delivery to the
overnight courier if sent by facsimile or overnight courier; and (d) subject to Section 3.1, if sent by
email on the earliest of a receipt of a delivery or read receipt email from the correct address, on
receipt of confirmation of receipt from the recipient or twenty-four (24) hours from delivery if sent
to the correct email address and no notice of delivery failure is received.  A Party may change its
address listed above by sending notice to the other Party in accordance with this Section 19.8.

19.9

Third-Party Beneficiaries.  None of the provisions of this Agreement shall be for the
benefit of or enforceable by any Third Party, including any creditor of either Party, (whether under
the Contracts (Rights of Third Parties) Act 1999 or otherwise); provided that [***] shall be a third
party  beneficiary  of  this  Agreement  to  the  extent  permitted  under  Applicable  Laws,  solely  to
enforce the Applied Patent Rights and/or Applied Technology (in each case, which are owned by
[***]).    Subject  to  the  foregoing  and  the  indemnification  obligations  set  forth  in  Sections  17.1
17.2,  and  17.3  which  shall  be  enforced  by  each  Party  with  respect  to  any  of  their  respective
indemnified parties, no Third Party shall obtain any right under any provision of this Agreement or
shall by reason of any such provision make any claim in respect of any debt, liability or obligation
(or otherwise) against either Party.

19.10 Binding Effect.  This Agreement shall be binding upon and inure to the benefit of

the Parties hereto and their respective heirs, successors and permitted assigns.

19.11 Performance by Affiliates.  To the extent that this Agreement imposes obligations
on Affiliates of a Party, such Party agrees to cause its Affiliates to perform such obligations, and
any breaches of this Agreement by any such Affiliate shall be deemed a breach by and enforceable
against such Party hereunder.  Advanz may use one or more of its Affiliates to exercise its rights or
perform its obligations and duties hereunder; provided that Advanz shall remain liable hereunder
for  the  prompt  payment  and  performance  of  all  of  its  obligations  hereunder,  including,  for  the
avoidance of doubt, in respect of any Net Sales of Products attributable to the Commercialization
activities of any of Advanz’s Affiliates or Sublicensees.

19.12 Further Assurance.  Each Party shall (at its own cost) do, execute or procure to be
done and executed all acts, deeds, documents and things as are reasonably necessary or desirable to
give full effect to this Agreement.

18

19.13 Counterparts.  This Agreement may be executed in any counterparts, each of which,
when executed, shall be deemed to be an original and which together shall constitute one and the
same document.  Signatures provided by facsimile transmission or in Adobe™ Portable Document
Format (PDF) sent by electronic mail shall be deemed to be original signatures.

19.14 Order of Precedence.  In the event of any conflict between:

(a)

the  Quality  Agreement  and  this  Agreement,  the  Quality  Agreement  shall  take

precedence with regard to matters affecting the quality of the Products;

(b)

the  Pharmacovigilance  Agreement  and  this  Agreement,  the  Pharmacovigilance
Agreement shall take precedence with regard to matters to any safety data matters relating to the
Products;

(c)

the  Sections  and  the  Exhibits  in  this  Agreement,  the  Sections  in  this  Agreement

shall take precedence over the Exhibits.

19.15 Equitable Remedies.  The Parties agree that irreparable harm, or damage for which
monetary  damages  would  not  be  an  adequate  remedy,  may  occur  in  the  event  that  any  of  the
provisions of this Agreement were not performed in accordance with their specific terms or were
otherwise breached.  It is accordingly agreed that, without limitation of other remedies which may
be available to a Party for breach of this Agreement by the other Party, the Parties shall be entitled
to seek equitable relief, including an injunction or injunctions to prevent or mitigate breaches of
this Agreement and to enforce specifically the terms and provisions of this Agreement.

19.16 Data Protection.  The Parties acknowledge that, to the extent that any personal data
is processed under the terms of this Agreement, each Party is a separate controller in respect of that
personal data and shall comply with all Applicable Laws in respect of data protection in relation to
the processing of that personal data.

19.17 Financial Stability.  Applied covenants and agrees that, so long as this Agreement
shall remain in effect, it will furnish to Advanz (a) within ninety (90) days after the end of each
fiscal year of Applied, a consolidated balance sheet and related statements of operations of Applied
and  its  controlled  Affiliates  (provided  that  “controlled”  shall  have  the  meaning  assigned  to  it  in
Section  1.10),  if  any,  as  of  the  close  of  such  fiscal  year  and  the  consolidated  results  of  its
operations  during  such  year  (it  being  understood  that  the  filing  by  Applied  of  annual  reports  on
Form  10-K  of  Applied  and  its  consolidated  Subsidiaries  with  the  Securities  and  Exchange
Commission shall satisfy the requirements of this Section 19.17 to the extent such annual reports
include  the  information  specified  herein)  and  (b)  within  forty-five  (45)  days  after  the  end  of  the
first  three  (3)  quarterly  periods  of  each  fiscal  year  of  Applied,  a  consolidated  balance  sheet  and
related  statements  of  operations  of  Applied  and  its  Subsidiaries,  if  any,  as  of  the  close  of  such
fiscal quarter and the consolidated results of its operations during such fiscal quarter and the then-
elapsed portion of the fiscal year (it being understood that the filing by Applied of quarterly reports
on  Form  10-Q  of  Applied  and  its  consolidated  Subsidiaries  with  the  Securities  and  Exchange
Commission shall satisfy the requirements of this Section 19.17 to the extent such quarterly reports
include  the  information  specified  herein).    In  this  Section  19.17,  financial  circumstances,  which
Advanz

18

reasonably  believes  will  materially  prejudice  Applied’s  ability  to  perform  its  obligations,  shall
constitute a “Financial Stability Event.”

Without  prejudice  to  any  other  rights  or  remedies  of  Advanz,  upon  the  occurrence  of  a
Financial Stability Event, Advanz shall have the right to require Applied to: (i) provide to Advanz
such relevant financial information (given the nature of the Financial Stability Event) relating to
Applied  as  Advanz  may  reasonably  require  (which  Applied  shall  promptly  provide);  and/or  (ii)
arrange  a  meeting  between  Advanz’s  CEO  and/or  CFO  (or  equivalent  role)  and  Applied’s  CEO
and/or CFO (or equivalent role) whom Applied shall make available for this purpose, as soon as
reasonably  practicable,  to  determine  whether  a  continuity  plan  is  required.    At  such  meeting,
discussions between the Parties shall take into consideration how to avoid placing Applied’s assets
including the Product in jeopardy and delaying access of the Product to patients.

Following such meeting, if Advanz determines that a continuity plan is required, Applied
shall  promptly  submit  to  Advanz  for  its  approval  (and  once  approved,  implement),  a  continuity
plan  to  deal  with  the  consequences  of  the  Financial  Stability  Event  as  soon  as  reasonably
practicable (the “Continuity Plan”).  If mutually agreed by both Parties, the Continuity Plan shall
include  rights  for  Advanz  to  exercise  some  or  all  of  its  Step-In  Rights  under  Section  8.14(a)
following issue of a Step-In Notice to Applied.

[Signature Page Follows]

18

IN  WITNESS  WHEREOF  the  Parties  hereto  have  caused  this  Agreement  to  be

executed by their duly authorized officers upon the date set out below.

APPLIED THERAPEUTICS, INC.

MERCURY PHARMA GROUP LIMITED

By: ___________________________

By:____________________________

Name:
Title:    

Name:
Title:    

 
Exhibit A

Compound

Exhibit A-1

[***]

Exhibit B

Applied Patent Rights

Exhibit B-1

[***]

Exhibit C

Licensed Trademarks

Exhibit C-1

Exhibit D

Territory

Austria,  Belgium,  Bulgaria,  Croatia,  Republic  of  Cyprus,  Czech  Republic,  Denmark,  Estonia,
Finland,  France,  Germany,  Greece,  Hungary,  Iceland,  Ireland,  Italy,  Latvia,  Liechtenstein,
Lithuania,  Luxembourg,  Malta,  Netherlands,  Norway,  Poland,  Portugal,  Romania,  Slovakia,
Slovenia, Spain, Sweden, Switzerland and the United Kingdom

Exhibit D-1

1.

2.

Columbia License

Miami License

Exhibit E

Third Party Licenses

Exhibit E-1

Exhibit F

Press Release

For immediate release

 ADVANZ  PHARMA  to  receive  exclusive  rights  from  Applied
Therapeutics to commercialise AT-007 (govorestat) in Europe

● ADVANZ PHARMA secures exclusive rights to register and commercialise AT-007, a

Phase  3  development  compound  for  the  treatment  of  several  rare  neurological

diseases,  including  Galactosemia  and  SORD  Deficiency,  in  the  European  Economic

Area, the UK, and Switzerland

● ADVANZ  PHARMA  will  leverage  its  existing  specialty,  hospital,  and  rare  disease

expertise  and  infrastructure  to  ensure  successful  commercialisation  and  patient

access

London,  UK  –  January  4,  2023:  ADVANZ  PHARMA  Corp.  (“ADVANZ”  or  “the  Company”),  a  UK

headquartered  global  pharmaceutical  company  with  a  strategic  focus  on  specialty,  hospital,  and  rare

disease medicines in Europe, today announced that it has entered into an exclusive agreement with Applied

Therapeutics,  a  clinical-stage  biopharmaceutical  company  developing  a  pipeline  of  novel  drug  candidates

against validated molecular targets in indications of high unmet medical need.

Under  the  terms  of  the  agreement,  Applied  Therapeutics  will  be  responsible  for  the  clinical  development

and supply of AT-007, while ADVANZ will manage the registration and commercialisation in the European

Economic Area, the UK, and Switzerland.

Steffen  Wagner,  CEO  of  ADVANZ,  commented:  “We  are  very  excited  to  announce  this  partnership  with

Applied  Therapeutics,  which  is  fully  aligned  with  ADVANZ’s  strategy  to  be  a  partner  of  choice  for

commercialisation of specialty, hospital, and rare disease medicines in Europe.”

Exhibit F-1

 
“We  believe  ADVANZ  PHARMA  is  an  ideal  partner  for  commercialisation  of  AT-007  in  Europe,”  said

Shoshana  Shendelman,  PhD,  Founder  and  CEO  of  Applied  Therapeutics.  “ADVANZ  PHARMA’s

commitment  to  improving  the  lives  of  patients  alongside  their  critical  infrastructure  and  expertise  in  rare

diseases positions them well for commercial success. This partnership brings us one step closer to making

AT-007 available to patients with Galactosemia and SORD Deficiency – both debilitating rare diseases with

no other therapies currently available.”

Susanna  El-Armale,  Chief  Corporate  Development  Officer  of  ADVANZ,  stated:  “This  partnership  with

Applied  Therapeutics  delivers  on  our  commitment  to  bring  innovative  products  to  market  that  serve  an

unmet medical need and it supports our ambition to build a strong product pipeline to drive ADVANZ’s mid-

and long-term growth.”

Ends

About AT-007

AT-007 is a central nervous system (CNS) penetrant Aldose Reductase inhibitor (ARI) in development for

the treatment of several rare neurological diseases, including Galactosemia, SORD Deficiency, and PMM2-

CDG.  In  clinical  trials,  AT-007  significantly  reduced  plasma  galactitol  levels  vs.  placebo  in  adults  and

children with Galactosemia. AT-007 is currently being studied in a Phase 3 clinical outcomes trial (ACTION-

Galactosemia  Kids)  in  children  ages  2-17  with  Galactosemia,  as  well  as  a  long-term  open-label  study  in

adults  with  Galactosemia.  In  a  pilot  study  in  adults  with  SORD  Deficiency,  AT-007  significantly  reduced

blood sorbitol levels. AT-007 is currently being studied in a Phase 3 trial (INSPIRE) investigating biomarker

efficacy and clinical outcomes in adults and children 16 years and older with SORD Deficiency. The drug

has been generally safe and well tolerated in all clinical studies to date.  

About ADVANZ PHARMA

ADVANZ  PHARMA  is  a  global  pharmaceutical  company  with  a  strategic  focus  on  specialty,  hospital,  and

rare  disease  medicines  in  Europe.  The  company  has  commercial  affiliates  in  Europe,  North  America  and

Australia,  and  a  Centre  of  Excellence  in  Mumbai,  India,  as  well  as  an  established  global  network  of

commercial partners throughout the rest of the world. With an agile and experienced team, including direct

sales, marketing, and medical capabilities across Europe’s major markets, Canada, and Australia, ADVANZ

PHARMA is committed to improving lives of patients by providing and enhancing the specialty, hospital, and

rare disease medicines they depend on. The company has a broad expertise in several therapeutic areas

including  hepatology,  gastroenterology,  critical  care,  anti-infectives,  endocrinology,  oncology,  and  more

broadly rare disease medicines, making ADVANZ PHARMA a partner of choice for the commercialisation of

specialty, hospital, and rare disease medicines.

For more information, please visit our Website or Linkedin.

For media inquiries, please contact:

Exhibit F-2

Courtney Baines

ADVANZ PHARMA Corp.  

Tel: +44 77641 7246 Email: courtney.baines@advanzpharma.com

Exhibit F-3

Applied Therapeutics Announces Partnership with Advanz Pharma for Commercialization of AT-007
(Govorestat) in Europe

●

Advanz Pharma will leverage its specialty, hospital, and rare disease expertise and infrastructure to

commercialize AT-007 in Europe for both Galactosemia and SORD Deficiency

Applied Therapeutics will receive milestone payments of over €130 million and 20% royalty

payments on net sales in Europe

Deal strengthens Applied Therapeutics’ capital position and extends cash runway through key

●

●

milestones

NEW  YORK,  January  4,  2023–  Applied  Therapeutics,  Inc.  (Nasdaq:  APLT),  a  clinical-stage
biopharmaceutical  company  developing  a  pipeline  of  novel  drug  candidates  against  validated  molecular
targets in indications of high unmet medical need, today announced a partnership with Advanz Pharma, a
pharmaceutical company with a strategic focus on commercialization of specialty, hospital, and rare disease
medicines, for commercialization of AT-007 (govorestat) in Europe.  

“We believe Advanz Pharma is an ideal partner for commercialization of AT-007 in Europe,” said Shoshana
Shendelman,  PhD,  Founder  and  CEO  of  Applied  Therapeutics.  “Advanz  Pharma’s  commitment  to
improving the lives of patients alongside their critical infrastructure and expertise in rare diseases positions
them well for commercial success.  This partnership brings us one step closer to making AT-007 available to
patients with Galactosemia and SORD Deficiency – both debilitating rare diseases with no other therapies
currently available – and strengthens Applied Therapeutics’ capital position.”

“We  are  pleased  to  partner  with  Applied  Therapeutics,”  said  Susanna  El-Armale,  Chief  Corporate
Development Officer of Advanz. “We believe that AT-007 represents a compelling scientific opportunity to
treat  rare  diseases,  including  Galactosemia  and  SORD  Deficiency.  This  partnership  delivers  on  our
commitment to bring innovative products to market that serve an unmet medical need and to build a strong
product pipeline to drive Advanz’s mid- and long-term growth.”

Under the terms of the agreement:

● Applied  Therapeutics  will  receive  certain  near-term  development  milestones  upon  clinical  trial
completion and marketing authorization in Europe as well as commercial sales milestones, which in
the aggregate amount to over €130 million, including €10 million upfront due upon signing.
● Applied Therapeutics will receive royalties on any future net sales of AT-007 in Europe of 20%.
● Applied  Therapeutics  will  continue  to  be  responsible  for  the  development,  manufacturing  and
supply  of  AT-007,  and  Advanz  Pharma  will  be  responsible  for  packaging,  distribution  and
commercialization in Europe.

● Advanz Pharma receives exclusive commercial rights in the European Economic Area, Switzerland,
and  the  UK  for  AT-007  in  Galactosemia  and  SORD  Deficiency,  with  certain  rights  to  future
indications for AT-007 in Europe.

About AT-007

AT-007 is a central nervous system (CNS) penetrant Aldose Reductase inhibitor (ARI) in development for
the treatment of several rare neurological diseases, including Galactosemia, SORD Deficiency, and PMM2-
CDG.  In  clinical  trials,  AT-007  significantly  reduced  plasma  galactitol  levels  vs.  placebo  in  adults  and
children  with  Galactosemia.    AT-007  is  currently  being  studied  in  a  Phase  3  clinical  outcomes  trial
(ACTION-Galactosemia Kids) in children ages 2-17 with Galactosemia, as well as a long-term open-label
study in adults with Galactosemia.  In a pilot study in adults with SORD Deficiency, AT-007 significantly
reduced blood sorbitol levels. AT-007 is currently being studied in a Phase 3 trial (INSPIRE) investigating

Exhibit F-4

biomarker efficacy and clinical outcomes in adults and children 16 years and older with SORD Deficiency.
The drug has been generally safe and well tolerated in all clinical studies to date.  

About Applied Therapeutics

Applied  Therapeutics  is  a  clinical-stage  biopharmaceutical  company  developing  a  pipeline  of  novel  drug
candidates against validated molecular targets in indications of high unmet medical need. The Company’s
lead drug candidate, AT-007, is a novel central nervous system penetrant Aldose Reductase Inhibitor (ARI)
for the treatment of CNS rare metabolic diseases, including Galactosemia, SORD Deficiency, and PMM2-
CDG.  The  Company  is  also  developing  AT-001,  a  novel  potent  ARI,  for  the  treatment  of  Diabetic
Cardiomyopathy, or DbCM, a fatal fibrosis of the heart. The preclinical pipeline also includes AT-003, an
ARI  designed  to  cross  through  the  back  of  the  eye  when  dosed  orally,  for  the  treatment  of  Diabetic
retinopathy.

learn  more,  please  visit  www.appliedtherapeutics.com  and  follow 

To 
@Applied_Tx.

the  company  on  Twitter

About Advanz Pharma

ADVANZ PHARMA is a global pharmaceutical company with a strategic focus on specialty, hospital, and
rare  disease  medicines  in  Europe  and  Canada.    The  company  has  commercial  affiliates  in  Europe,  North
America  and  Australia,  and  a  Centre  of  Excellence  in  Mumbai,  India,  as  well  as  an  established  global
network  of  commercial  partners  throughout  the  rest  of  the  world.  With  an  agile  and  experienced  team,
including  direct  sales,  marketing,  and  medical  capabilities  across  Europe’s  major  markets,  Canada,  and
Australia, ADVANZ PHARMA is committed to improving lives of patients by providing and enhancing the
specialty,  hospital,  and  rare  disease  medicines  they  depend  on.    The  company  has  a  broad  expertise  in
several  therapeutic  areas  including  hepatology,  gastroenterology,  CNS,  critical  care,  anti-infectives,
endocrinology, oncology, and more broadly rare disease medicines, making ADVANZ PHARMA a partner
of choice for the commercialization of specialty, hospital, and rare disease medicines.

Forward-Looking Statements

This press release contains “forward-looking statements” that involve substantial risks and uncertainties for
purposes  of  the  safe  harbor  provided  by  the  Private  Securities  Litigation  Reform  Act  of  1995.  Any
statements,  other  than  statements  of  historical  fact,  included  in  this  press  release  regarding  the  strategy,
future operations, prospects, plans and objectives of management, including words such as “may,” “will,”
“expect,”  “anticipate,”  “plan,”  “intend,”  and  similar  expressions  (as  well  as  other  words  or  expressions
referencing  future  events,  conditions  or  circumstances)  are  forward-looking  statements.  These  include,
without  limitation,  statements  regarding  (i)  the  anticipated  benefits  of  the  Company’s  partnership  with
Advanz Pharma and (ii) the expected development milestone payments. Forward-looking statements in this
release  involve  substantial  risks  and  uncertainties  that  could  cause  actual  results  to  differ  materially  from
those expressed or implied by the forward-looking statements, and we, therefore cannot assure you that our
plans, intentions, expectations or strategies will be attained or achieved.

Such risks and uncertainties include, without limitation, (i) our plans to develop, market and commercialize
our product candidates, (ii) the initiation, timing, progress and results of our current and future preclinical
studies and clinical trials and our research and development programs, (iii) our ability to take advantage of
expedited  regulatory  pathways  for  any  of  our  product  candidates,  (iv)  our  estimates  regarding  expenses,
future  revenue,  capital  requirements  and  needs  for  additional  financing,  (v)  our  ability  to  successfully
acquire or license additional product candidates on reasonable terms and advance product candidates into,
and successfully complete, clinical studies, (vi) our ability to maintain and establish collaborations or obtain

Exhibit F-5

additional  funding,  (vii)  our  ability  to  obtain  and  timing  of  regulatory  approval  of  our  current  and  future
product  candidates,  (viii)  the  anticipated  indications  for  our  product  candidates,  if  approved,  (ix)  our
expectations  regarding  the  potential  market  size  and  the  rate  and  degree  of  market  acceptance  of  such
product candidates, (x) our ability to fund our working capital requirements and expectations regarding the
sufficiency of our capital resources, (xi) the implementation of our business model and strategic plans for
our business and product candidates, (xii) our intellectual property position and the duration of our patent
rights, (xiii) developments or disputes concerning our intellectual property or other proprietary rights, (xiv)
our expectations regarding government and third-party payor coverage and reimbursement, (xv) our ability
to  compete  in  the  markets  we  serve,  (xvi)  the  impact  of  government  laws  and  regulations  and  liabilities
thereunder,  (xvii)  developments  relating  to  our  competitors  and  our  industry,  (xvii)  the  impact  of  the
COVID-19 pandemic on the timing and progress of our ongoing clinical trials and our business in general
and (xiv) other factors that may impact our financial results. In light of the significant uncertainties in these
forward-looking statements, you should not rely upon forward-looking statements as predictions of future
events. Although we believe that we have a reasonable basis for each forward-looking statement contained
in  this  press  release,  we  cannot  guarantee  that  the  future  results,  levels  of  activity,  performance  or  events
and circumstances reflected in the forward-looking statements will be achieved or occur at all. Factors that
may cause actual results to differ from those expressed or implied in the forward-looking statements in this
press release are discussed in our filings with the U.S. Securities and Exchange Commission, including the
“Risk  Factors”  contained  therein.  Except  as  otherwise  required  by  law,  we  disclaim  any  intention  or
obligation to update or revise any forward-looking statements, which speak only as of the date they were
made, whether as a result of new information, future events or circumstances or otherwise.

Contacts

Investors:

Maghan Meyers
(212) 600-1902
appliedtherapeutics@argotpartners.com

Media:
media@appliedtherapeutics.com  

Applied Therapeutics, Inc.

Exhibit F-6

[***]

Exhibit G

COGs Components

Exhibit G-1

Exhibit H

Third Party License Flow-Down Provisions

[***]

Exhibit H-1

[***]

Exhibit I

Cost of Goods Analysis

Exhibit I-1

Exhibit J

Affiliate Sublicensees as at Effective Date

[***]

Exhibit J-1

Exhibit 23.1

Consent of Independent Registered Public Accounting Firm

We consent to the incorporation by reference in the following Registration Statements:

● Registration Statement (Form S-8 No. 333-231618) of Applied Therapeutics, Inc.,
● Registration Statement (Form S-8 No. 333-255018) of Applied Therapeutics, Inc, and
● Registration Statement (Form S-3 No. 333-238948) of Applied Therapeutics, Inc.

of our report dated March 23, 2023, with respect to the financial statements of Applied Therapeutics, Inc. included in this Annual
Report (Form 10-K) of Applied Therapeutics for the year ended December 31, 2022.

/s/ Ernst & Young LLP

New York, New York
March 23, 2023

Exhibit 31.1

CERTIFICATIONS

The undersigned certifies that:

1.           I have reviewed this Form 10-K of Applied Therapeutics, Inc.;

2.           Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material  fact  necessary  to  make  the  statements  made,  in  light  of  the  circumstances  under  which  such
statements were made, not misleading with respect to the period covered by this report;

3.           Based on my knowledge, the financial statements, and other financial information included in this report,
fairly  present  in  all  material  respects  the  financial  condition,  results  of  operations  and  cash  flows  of  the
registrant as of, and for, the periods presented in this report;

4.           The registrant’s other certifying officer(s) and I are responsible for establishing and maintaining disclosure
controls and procedures (as defined in Exchange Act Rules 13a-15(e) and 15d-15(e)) and internal control over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

(a)          Designed such disclosure controls and procedures, or caused such disclosure controls and procedures
to be designed under our supervision, to ensure that material information relating to the registrant,
including  its  consolidated  subsidiaries,  is  made  known  to  us  by  others  within  those  entities,
particularly during the period in which this report is being prepared;

(b)                    Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over
financial reporting to be designed under our supervision, to provide reasonable assurance regarding
the reliability of financial reporting and the preparation of financial statements for external purposes
in accordance with generally accepted accounting principles;

(c)          Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in
this  report  our  conclusions  about  the  effectiveness  of  the  disclosure  controls  and  procedures,  as  of
the end of the period covered by this report based on such evaluation; and

(d)          Disclosed in this report any change in the registrant’s internal control over financial reporting that
occurred during the registrant’s most recent fiscal quarter (the registrant’s fourth fiscal quarter in the
case of an annual report) that has materially affected, or is reasonably likely to materially affect, the
registrant’s internal control over financial reporting; and

5.                      The  registrant’s  other  certifying  officer(s)  and  I  have  disclosed,  based  on  our  most  recent  evaluation  of
internal control over financial reporting, to the registrant’s auditors and the audit committee of the registrant’s
board of directors (or persons performing the equivalent functions):

(a)          All significant deficiencies and material weaknesses in the design or operation of internal control
over  financial  reporting  which  are  reasonably  likely  to  adversely  affect  the  registrant’s  ability  to
record, process, summarize and report financial information; and

(b)                 Any  fraud,  whether  or  not  material,  that  involves  management  or  other  employees  who  have  a

significant role in the registrant’s internal control over financial reporting.

Date: March 23, 2023

By:

/s/ Shoshana
Shendelman
Name: Shoshana Shendelman,

Title:

Ph.D.
Chief Executive Officer
(Principal Executive
Officer)

 
Exhibit 31.2

CERTIFICATIONS

The undersigned certifies that:

1.           I have reviewed this Form 10-K of Applied Therapeutics, Inc.;

2.           Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material  fact  necessary  to  make  the  statements  made,  in  light  of  the  circumstances  under  which  such
statements were made, not misleading with respect to the period covered by this report;

3.           Based on my knowledge, the financial statements, and other financial information included in this report,
fairly  present  in  all  material  respects  the  financial  condition,  results  of  operations  and  cash  flows  of  the
registrant as of, and for, the periods presented in this report;

4.           The registrant’s other certifying officer(s) and I are responsible for establishing and maintaining disclosure
controls and procedures (as defined in Exchange Act Rules 13a-15(e) and 15d-15(e)) and internal control over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

(a)          Designed such disclosure controls and procedures, or caused such disclosure controls and procedures
to be designed under our supervision, to ensure that material information relating to the registrant,
including  its  consolidated  subsidiaries,  is  made  known  to  us  by  others  within  those  entities,
particularly during the period in which this report is being prepared;

(b)                    Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over
financial reporting to be designed under our supervision, to provide reasonable assurance regarding
the reliability of financial reporting and the preparation of financial statements for external purposes
in accordance with generally accepted accounting principles;

(c)          Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in
this  report  our  conclusions  about  the  effectiveness  of  the  disclosure  controls  and  procedures,  as  of
the end of the period covered by this report based on such evaluation; and

(d)          Disclosed in this report any change in the registrant’s internal control over financial reporting that
occurred during the registrant’s most recent fiscal quarter (the registrant’s fourth fiscal quarter in the
case of an annual report) that has materially affected, or is reasonably likely to materially affect, the
registrant’s internal control over financial reporting; and

5.                      The  registrant’s  other  certifying  officer(s)  and  I  have  disclosed,  based  on  our  most  recent  evaluation  of
internal control over financial reporting, to the registrant’s auditors and the audit committee of the registrant’s
board of directors (or persons performing the equivalent functions):

(a)          All significant deficiencies and material weaknesses in the design or operation of internal control
over  financial  reporting  which  are  reasonably  likely  to  adversely  affect  the  registrant’s  ability  to
record, process, summarize and report financial information; and

(b)                 Any  fraud,  whether  or  not  material,  that  involves  management  or  other  employees  who  have  a

significant role in the registrant’s internal control over financial reporting.

Date: March 23, 2023

/s/Steven Ortega

By:
Name:Steven Ortega
Title: Chief Accounting Officer

(Principal Accounting Officer
and Interim Principal
Financial Officer)

CERTIFICATION

Exhibit 32.1

Pursuant  to  the  requirement  set  forth  in  Rule  13a-14(b)  of  the  Securities  Exchange  Act  of  1934,  as  amended,  (the
“Exchange  Act”)  and  Section  1350  of  Chapter  63  of  Title  18  of  the  United  States  Code  (18  U.S.C.  §1350),  the
undersigned hereby certifies that, to the best of their knowledge:

1.

2.

The Annual Report on Form 10-K of Applied Therapeutics, Inc. (the “Company”) for the fiscal year ended
December  31,  2022,  to  which  this  Certification  is  attached  as  Exhibit  32.1  (the  “Annual  Report”),  fully
complies with the requirements of Section 13(a) or Section 15(d) of the Exchange Act; and

The  information  contained  in  the  Annual  Report  fairly  presents,  in  all  material  respects,  the  financial
condition and results of operations of the Company.

Dated: March 23, 2023

By:

/s/ Shoshana
Shendelman
Name: Shoshana Shendelman,

Title:

Ph.D.
Chief Executive Officer
(Principal Executive
Officer)

 
CERTIFICATION

Exhibit 32.2

Pursuant  to  the  requirement  set  forth  in  Rule  13a-14(b)  of  the  Securities  Exchange  Act  of  1934,  as  amended,  (the
“Exchange  Act”)  and  Section  1350  of  Chapter  63  of  Title  18  of  the  United  States  Code  (18  U.S.C.  §1350),  the
undersigned hereby certifies that, to the best of their knowledge:

1.

2.

The Annual Report on Form 10-K of Applied Therapeutics, Inc. (the “Company”) for the fiscal year ended
December  31,  2022,  to  which  this  Certification  is  attached  as  Exhibit  32.2  (the  “Annual  Report”),  fully
complies with the requirements of Section 13(a) or Section 15(d) of the Exchange Act; and

The  information  contained  in  the  Annual  Report  fairly  presents,  in  all  material  respects,  the  financial
condition and results of operations of the Company.

Dated: March 23, 2023

/s/ Steven Ortega

By:
Name: Steven Ortega
Title:

Chief Accounting
Officer
(Principal Accounting
Officer and Interim
Principal Financial
Officer)