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Intercept Pharmaceuticals

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FY2020 Annual Report · Intercept Pharmaceuticals
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UNITED STATES
SECURITIES AND EXCHANGE COMMISSION
WASHINGTON, D.C. 20549

FORM 10-K

(Mark One)

☒   ANNUAL REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the fiscal year ended December 31, 2020

OR

☐   TRANSITION REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the transition period from             to

Commission file number: 001-35668

Intercept Pharmaceuticals, Inc.
(Exact Name of Registrant as Specified in Its Charter)

Delaware
(State or Other Jurisdiction of
Incorporation or Organization)

22-3868459
(I.R.S. Employer
Identification No.)

10 Hudson Yards, 37th Floor
New York, NY 10001
(Address of Principal Executive Offices and Zip Code)
(646) 747-1000
(Registrant’s Telephone Number, Including Area Code)

Securities registered pursuant to Section 12(b) of the Act:

Title of each class

Common Stock, par value $0.001 per share

Trading Symbol(s)

ICPT

Name of each exchange on which registered

Nasdaq Global Select Market

Securities registered pursuant to Section 12(g) of the Act: None

Indicate by check mark if the registrant is a well-known seasoned issuer, as defined in Rule 405 of the Securities Act. Yes ☒ No ☐

Indicate by check mark if the registrant is not required to file reports pursuant to Section 13 or Section 15(d) of the Act. Yes ☐ No ☒

Indicate  by  check  mark  whether  the  registrant  (1)  has  filed  all  reports  required  to  be  filed  by  Section  13  or  15(d)  of  the  Securities  Exchange  Act  of  1934  during  the
preceding 12 months (or for such shorter period that the registrant was required to file such reports), and (2) has been subject to such filing requirements for the past 90 days. Yes
☒ No ☐

Indicate by check mark whether the registrant has submitted electronically every Interactive Data File required to be submitted pursuant to Rule 405 of Regulation S-T (§

232.405 of this chapter) during the preceding 12 months (or for such shorter period that the registrant was required to submit such files).Yes ☒ No ☐

Indicate by check mark whether the registrant is a large accelerated filer, an accelerated filer, a non-accelerated filer, a smaller reporting company, or an emerging growth

company. See the definitions of “large accelerated filer,” “accelerated filer,” “smaller reporting company,” and “emerging growth company” in Rule 12b-2 of the Exchange Act:

       Large accelerated filer
       Non-accelerated filer

☒
☐

Accelerated filer
Smaller reporting company
Emerging growth company

☐
☐
☐

If  an  emerging  growth  company,  indicate  by  check  mark  if  the  registrant  has  elected  not  to  use  the  extended  transition  period  for  complying  with  any  new  or  revised

financial accounting standards provided pursuant to Section 13(a) of the Exchange Act. ☐

Indicate by check mark whether the registrant has filed a report on and attestation to its management’s assessment of the effectiveness of its internal control over financial

reporting under Section 404(b) of the Sarbanes-Oxley Act (15 U.S.C. 7262(b)) by the registered public accounting firm that prepared or issued its audit report. ☒

Indicate by check mark whether the registrant is a shell company (as defined in Rule 12b-2 of the Act).Yes ☐ No ☒

The aggregate market value of the registrant’s common stock held by non-affiliates as of June 30, 2020, the last business day of the registrant’s most recently completed
second fiscal quarter, was $1,259.3 million (computed by reference to the closing price of $47.91 on such date as reported by the Nasdaq Global Select Market). Common stock
held by our executive officers, directors and certain stockholders as of such date has been excluded from this calculation because such persons may be deemed to be affiliates.
This determination of affiliate status is not necessarily a conclusive determination for other purposes.

The number of shares of the registrant’s common stock outstanding as of December 31, 2020 was 33,015,614.

DOCUMENTS INCORPORATED BY REFERENCE
Certain information required by Part III of this Annual Report on Form 10-K is incorporated by reference to the registrant’s definitive proxy statement related to its 2021

Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the fiscal year covered by this Annual Report on Form 10-K.

    
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Part I.

Intercept Pharmaceuticals, Inc.
Annual Report on Form 10-K
For the Fiscal Year Ended December 31, 2020

TABLE OF CONTENTS

Business

Item 1.
Item 1A. Risk Factors
Item 1B. Unresolved Staff Comments
Item 2.
Item 3.
Item 4. Mine Safety Disclosures

Properties
Legal Proceedings

Part II.

Item 5. Market for Registrant’s Common Equity, Related Stockholder Matters and Issuer Purchases of Equity

Securities
Selected Financial Data

Item 6.
Item 7. Management’s Discussion and Analysis of Financial Condition and Results of Operations
Item 7A. Quantitative and Qualitative Disclosures About Market Risk
Item 8.
Item 9.
Item 9A. Controls and Procedures
Item 9B. Other Information

Financial Statements and Supplementary Data
Changes in and Disagreements With Accountants on Accounting and Financial Disclosure

Part III.

Item 10. Directors, Executive Officers and Corporate Governance
Item 11. Executive Compensation
Item 12. Security Ownership of Certain Beneficial Owners and Management and Related Stockholder Matters
Item 13. Certain Relationships and Related Transactions, and Director Independence
Item 14. Principal Accounting Fees and Services

Part IV.

Item 15. Exhibits and Financial Statement Schedules
Item 16. Form 10-K Summary
Signatures

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Unless the context otherwise requires, references in this Annual Report on Form 10-K to “we,” “our,” “us” and the
“Company” refer, collectively, to Intercept Pharmaceuticals, Inc., a Delaware corporation, and its consolidated subsidiaries.

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CAUTIONARY NOTE REGARDING FORWARD-LOOKING STATEMENTS

This  Annual  Report  on  Form  10-K  contains  forward-looking  statements,  including,  but  not  limited  to,  statements
regarding the progress, timing and results of our clinical trials, including our clinical trials for the treatment of nonalcoholic
steatohepatitis  (“NASH”),  the  safety  and  efficacy  of  our  approved  product,  Ocaliva  (obeticholic  acid  or  “OCA”)  for
primary biliary cholangitis (“PBC”), and our product candidates, including OCA for liver fibrosis due to NASH, the timing
and acceptance of our regulatory filings and the potential approval of OCA for liver fibrosis due to NASH, the review of
our  New  Drug  Application  for  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH  by  the  U.S.  Food  and  Drug
Administration  (the  “FDA”),  our  intent  to  work  with  the  FDA  to  address  the  issues  raised  in  a  complete  response  letter
(“CRL”),  the  potential  commercial  success  of  OCA,  as  well  as  our  strategy,  future  operations,  future  financial  position,
future revenue, projected costs, financial guidance, prospects, plans and objectives.

These  statements  constitute  forward-looking  statements  within  the  meaning  of  Section  27A  of  the  Securities  Act  of
1933,  as  amended,  and  Section  21E  of  the  Securities  Exchange  Act  of  1934,  as  amended.  The  words  “anticipate,”
“believe,”  “estimate,”  “expect,”  “intend,”  “may,”  “plan,”  “predict,”  “project,”  “target,”  “potential,”  “will,”  “would,”
“could,”  “should,”  “possible,”  “continue”  and  similar  expressions  are  intended  to  identify  forward-looking  statements,
although  not  all  forward-looking  statements  contain  these  identifying  words.  Readers  are  cautioned  not  to  place  undue
reliance on these forward-looking statements, which speak only as of their dates, and we undertake no obligation to update
any  forward-looking  statement  except  as  required  by  law.  These  forward-looking  statements  are  based  on  estimates  and
assumptions by our management that, although believed to be reasonable, are inherently uncertain and subject to a number
of risks.

The following represent some, but not necessarily all, of the factors that could cause actual results to differ materially

from historical results or those anticipated or predicted by our forward-looking statements:

● our ability to successfully commercialize Ocaliva for PBC;

● our  ability  to  maintain  our  regulatory  approval  of  Ocaliva  for  PBC  in  the  United  States,  Europe,  Canada,

Israel, Australia and other jurisdictions in which we have or may receive marketing authorization;

● our ability to timely and cost-effectively file for and obtain regulatory approval of our product candidates on
an accelerated basis or at all, including OCA for liver fibrosis due to NASH following the issuance of the
CRL  by  the  FDA;  any  advisory  committee  recommendation  or  dispute  resolution  determination  that  our
product candidates, including OCA for liver fibrosis due to NASH, should not be approved or approved only
under  certain  conditions;  or  any  future  determination  that  the  regulatory  applications  and  subsequent
information  we  submit  for  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  do  not
contain adequate clinical or other data or meet applicable regulatory requirements for approval;

● conditions that may be imposed by regulatory authorities on our marketing approvals for our products and
product candidates, including OCA for liver fibrosis due to NASH, such as the need for clinical outcomes
data (and not just results based on achievement of a surrogate endpoint), any risk mitigation programs such
as  a  REMS,  and  any  related  restrictions,  limitations  and/or  warnings  contained  in  the  label  of  any  of  our
products or product candidates;

● any potential side effects associated with Ocaliva for PBC, OCA for liver fibrosis due to NASH or our other
product candidates that could delay or prevent approval, require that an approved product be taken off the
market, require the inclusion of safety warnings or precautions, or otherwise limit the sale of such product or
product  candidate,  including  in  connection  with  the  newly  identified  safety  signal  ("NISS")  relating  to
Ocaliva identified by the FDA in May 2020;

● the  initiation,  timing,  cost,  conduct,  progress  and  results  of  our  research  and  development  activities,
preclinical studies and clinical trials, including any issues, delays or failures in identifying patients, enrolling
patients,  treating  patients,  retaining  patients,  meeting  specific  endpoints  in  the  jurisdictions  in  which  we
intend to seek approval or completing and timely reporting the results of our NASH or PBC clinical trials;

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● the outcomes of ongoing discussions with the FDA and the European Medicines Agency ("EMA") regarding

the feasibility of the COBALT and 401 trials;

● our ability to establish and maintain relationships with, and the performance of, third-party manufacturers,
contract  research  organizations  and  other  vendors  upon  whom  we  are  substantially  dependent  for,  among
other things, the manufacture and supply of our products, including Ocaliva for PBC and, if approved, OCA
for liver fibrosis due to NASH, and our clinical trial activities;

● our  ability  to  identify,  develop  and  successfully  commercialize  our  products  and  product  candidates,

including our ability to successfully launch OCA for liver fibrosis due to NASH, if approved;

● our  ability  to  obtain  and  maintain  intellectual  property  protection  for  our  products  and  product  candidates,
including  our  ability  to  cost-effectively  file,  prosecute,  defend  and  enforce  any  patent  claims  or  other
intellectual property rights;

● the  size  and  growth  of  the  markets  for  our  products  and  product  candidates  and  our  ability  to  serve  those

markets;

● the degree of market acceptance of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH or

our other product candidates among physicians, patients and healthcare payors;

● the  availability  of  adequate  coverage  and  reimbursement  from  governmental  and  private  healthcare  payors
for our products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH, and our
ability to obtain adequate pricing for such products;

● our ability to establish and maintain effective sales, marketing and distribution capabilities, either directly or

through collaborations with third parties;

● competition from existing drugs or new drugs that become available;

● our ability to prevent system failures, data breaches or violations of data protection laws;

● costs  and  outcomes  relating  to  any  disputes,  governmental  inquiries  or  investigations,  regulatory
proceedings,  legal  proceedings  or  litigation,  including  any  securities,  intellectual  property,  employment,
product liability or other litigation;

● our collaborators’ election to pursue research, development and commercialization activities;

● our  ability  to  establish  and  maintain  relationships  with  collaborators  with  development,  regulatory  and

commercialization expertise;

● our need for and ability to generate or obtain additional financing;

● our estimates regarding future expenses, revenues and capital requirements and the accuracy thereof;

● our use of cash and short-term investments;

● our ability to acquire, license and invest in businesses, technologies, product candidates and products;

● our ability to attract and retain key personnel to manage our business effectively;

● our ability to manage the growth of our operations, infrastructure, personnel, systems and controls;

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● our ability to obtain and maintain adequate insurance coverage;

● the  impact  of  COVID-19,  including  any  impact  on  our  results  of  operations  or  financial  position,  related
quarantines and government actions, delays relating to our regulatory applications, disruptions relating to our
ongoing clinical trials or involving our contract research organizations, study sites or other clinical partners,
disruptions  relating  to  our  supply  chain  or  involving  our  third-party  manufacturers,  distributors  or  other
distribution partners, facility closures or other restrictions, and the extent and duration thereof;

● the  impact  of  general  U.S.  and  foreign  economic,  industry,  market,  regulatory  or  political  conditions,

including the potential impact of Brexit; and

● the other risks and uncertainties identified under the captions “Risk Factors” and “Management’s Discussion
and  Analysis  of  Financial  Condition  and  Results  of  Operations”  and  elsewhere  in  this  Annual  Report  on
Form 10-K and in our other periodic filings filed with the U.S. Securities and Exchange Commission.

NOTE REGARDING TRADEMARKS

The Intercept Pharmaceuticals® name and logo and the Ocaliva® name and logo are either registered or unregistered
trademarks or trade names of the Company in the United States and/or other countries. All other trademarks, trade names
and service marks appearing in this Annual Report on Form 10-K are the property of their respective owners. Solely for
convenience, trademarks and trade names referred to in this Annual Report on Form 10-K may appear without the ® and
™ symbols, but those references are not intended to indicate, in any way, that we will not assert, to the fullest extent under
applicable law, our rights or that the applicable owner will not assert its rights to these trademarks and trade names.

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SUMMARY RISK FACTORS

Investing in our securities involves a high degree of risk. Investors should carefully consider the risks and uncertainties
discussed under the caption “Risk Factors” and elsewhere in this Annual Report on Form 10-K before deciding whether to
invest in our securities. The following is a list of some of these risks:

Risks Related to Our Financial Position and Need for Additional Capital

● We are currently dependent on the successful commercialization of Ocaliva for PBC. To the extent Ocaliva is
not  commercially  successful,  our  business,  financial  condition  and  results  of  operations  may  be  materially
and adversely affected and the price of our common stock may decline.

● We  have  never  been  profitable.  We  expect  to  incur  losses  for  the  foreseeable  future,  and  we  may  never

achieve or sustain profitability.

● We will require substantial additional funding, which may not be available to us on acceptable terms, if at all.

If adequate funds are not available to us, we may be required to delay, limit, reduce or cease our operations.
● Raising  additional  capital  may  cause  dilution  to  our  stockholders,  restrict  our  operations  or  require  us  to

relinquish rights to our technologies or product candidates.

● We have a limited operating history as a commercial organization, which may make it difficult to predict our
future performance, and we expect to continue to face a number of factors that may cause operating results to
fluctuate.

Risks Related to the Development and the Regulatory Review and
Approval of Our Products and Product Candidates

● We  cannot  be  certain  whether  Ocaliva  will  receive  full  approval  for  PBC  in  jurisdictions  where  it  has
previously  received  accelerated  or  conditional  approval,  or  that  Ocaliva  will  be  approved  for  PBC  in  any
jurisdictions beyond those in which it is currently approved. Furthermore, OCA may not be approved on an
accelerated basis, or at all, for NASH or any other indication beyond PBC and we may not receive regulatory
approval  for  any  other  product  candidate.  Without  regulatory  approval,  we  will  not  be  able  to  market  and
commercialize our product candidates.

● We are developing product candidates for the treatment of rare diseases or diseases for which there are no or
limited therapies, such as PBC and NASH, and for some of which there is little clinical experience, and our
development approach involves new endpoints and methodologies. As a result, there is a heightened risk that
we will not be able to gain agreement with regulatory authorities regarding an acceptable development plan,
that the outcome of our clinical trials will not be favorable or that, even if favorable, regulatory authorities
may not find the results of our clinical trials to be sufficient for marketing approval.

● Delays  or  difficulties  in  the  commencement,  enrollment  and  completion  of  our  clinical  trials  and  studies
could  increase  our  product  development  costs  and  delay,  limit  or  prevent  us  from  obtaining  regulatory
approval for OCA and our other product candidates.

● COVID-19 could materially and adversely affect our clinical trials.
● Failure can occur at any stage of clinical development. The results of earlier clinical trials are not necessarily
predictive of future results and any product candidate we or our collaborators advance through clinical trials,
including  OCA,  may  not  have  favorable  results  in  later  clinical  trials  or  receive  or  maintain  regulatory
approval.

● Our product candidates may have undesirable side effects which may delay or prevent marketing approval,
or,  if  approval  is  received,  require  that  our  products  be  taken  off  the  market  or  include  new  or  additional
safety  warnings.  Any  such  events  may  limit  our  existing  and  future  product  sales  and  materially  and
adversely affect our business, financial condition and results of operations.

● We may not be able to obtain or, if approved, maintain orphan drug exclusivity for our approved products or

product candidates, which could cause our revenues to suffer.

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Risks Related to the Commercialization of Our Products

● Sales of Ocaliva may be adversely affected by safety and labeling changes required by the FDA.
● We are subject to uncertainty relating to pricing and reimbursement. Failure to obtain or maintain adequate
coverage, pricing and reimbursement for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved,
or  our  other  future  approved  products,  if  any,  could  have  a  material  adverse  impact  on  our  ability  to
commercialize such products.

● Legislative and regulatory healthcare reform may adversely affect our business.
● Ocaliva  and  our  other  future  approved  products,  if  any,  may  not  achieve  broad  market  acceptance  among
physicians,  patients  and  healthcare  payors,  and  revenues  generated  from  their  sales  may  be  limited  as  a
result.

● If  we  fail  to  develop  OCA  for  additional  indications  such  as  NASH,  our  commercial  opportunity  will  be

limited.

Risks Related to Our Business and Strategy

● We  depend  on  third-party  contractors  for  a  substantial  portion  of  our  operations  and  may  not  be  able  to

control their work as effectively as if we performed these functions ourselves.

● We  face  rapid  technological  change  and  competition  from  other  biotechnology  and  pharmaceutical

companies. Our operating results will suffer if we fail to compete effectively.

● Our business and operations would suffer in the event of system failures, data breaches or violations of data

protection laws.

Risks Related to Our Intellectual Property

● It is difficult and costly to protect our proprietary rights, and we may not be able to ensure their protection. If
our patent position does not adequately protect our products such as Ocaliva and product candidates such as
OCA for liver fibrosis due to NASH, others may compete against us more directly, which could harm our
business, possibly materially.

● If  we  do  not  obtain  protection  under  the  Hatch-Waxman  Act  in  the  United  States  (and  similar  legislation
outside of the United States) extending the terms of our patents and/or providing data or other exclusivity for
our products and product candidates, our business may be materially harmed.

● We  may  incur  substantial  costs  as  a  result  of  litigation  or  other  proceedings  relating  to  patent  and  other
intellectual  property  rights,  and  such  litigation  may  divert  the  attention  of  our  management  and  scientific
personnel and adversely affect our development and commercialization efforts.

Risks Related to Our Indebtedness

● Servicing our debt will require significant amounts of cash, and we may not have sufficient cash flow from

our business to effectively service our debt.

● We may incur substantially more debt or take other actions that would affect our ability to pay the principal

of and interest on our debt.

Risks Related to Ownership of Our Common Stock

● We have previously been, and are currently, subject to securities class action litigation and may be subject to
similar or other litigation in the future. Such matters can be expensive, time-consuming and have a material
adverse effect on our business, results of operations and financial condition.

● Our stock price has been and may in the future be volatile, which could cause holders of our common stock

to incur substantial losses.

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Item 1.   Business

Overview

PART I

We are a biopharmaceutical company focused on the development and commercialization of novel therapeutics to treat
progressive non-viral liver diseases with high unmet medical need utilizing our proprietary bile acid chemistry. Our first
marketed  product,  Ocaliva®  (obeticholic  acid  or  “OCA”),  is  a  farnesoid  X  receptor  (“FXR”)  agonist  approved  in  the
United States, the European Union and several other jurisdictions for the treatment of primary biliary cholangitis (“PBC”)
in combination with ursodeoxycholic acid (“UDCA”) in adults with an inadequate response to UDCA or as monotherapy
in adults unable to tolerate UDCA. In addition to commercializing OCA for PBC under the Ocaliva brand name, we are
currently  developing  OCA  for  additional  indications,  including  nonalcoholic  steatohepatitis  (“NASH”).  We  are  also
developing other product candidates in various stages of clinical and preclinical development. We believe that OCA and
our other product candidates have the potential to treat orphan and other more prevalent liver diseases such as NASH for
which there are currently limited therapeutic options.

Ocaliva  was  approved  for  PBC  by  the  U.S.  Food  and  Drug  Administration  (“FDA”)  in  May  2016  under  the
accelerated approval pathway. We commenced sales and marketing of Ocaliva in the United States shortly after receiving
approval,  and  Ocaliva  is  now  available  to  U.S.  patients  primarily  through  a  network  of  specialty  pharmacy  distributors.
Ocaliva received conditional approval for PBC from the European Commission in December 2016 and we commenced our
European  commercial  launch  in  January  2017.  We  have  submitted  dossiers  and  obtained,  or  are  otherwise  pursuing,
reimbursement from a number of national authorities in Europe. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia, and
we are pursuing marketing approval of Ocaliva for PBC in our other international target markets. Ocaliva received orphan
drug designation in both the United States and the European Union for the treatment of PBC.

Our  lead  product  candidate  is  OCA  for  the  potential  treatment  of  NASH.  In  February  2019,  we  announced  topline
results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in  patients  with  liver
fibrosis due to NASH, known as the REGENERATE trial. In the primary efficacy analysis, once-daily OCA 25 mg met the
primary endpoint agreed with the FDA of fibrosis improvement by at least one stage with no worsening of NASH at the
planned  18-month  interim  analysis.  Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most  common
were consistent with the known profile of OCA. Interim analysis results at 18 months were based on surrogate endpoints
and  the  impact  on  clinical  outcomes  has  not  been  confirmed.  The  REGENERATE  trial  is  ongoing  and  is  expected  to
continue through clinical outcomes for verification and description of the clinical benefit of OCA. OCA also achieved the
primary  endpoint  in  a  Phase  2b  clinical  trial  for  the  treatment  of  NASH  that  completed  in  late  July  2014,  known  as  the
FLINT trial, which was sponsored by the U.S. National Institute of Diabetes and Digestive and Kidney Diseases, a part of
the National Institutes of Health. OCA has received breakthrough therapy designation from the FDA for the treatment of
NASH  patients  with  liver  fibrosis.  In  September  2019,  we  submitted  a  New  Drug  Application  (“NDA”)  to  the  FDA
seeking accelerated approval of OCA for liver fibrosis due to NASH. In November 2019, the FDA accepted our NDA for
filing and granted a priority review designation of OCA for liver fibrosis due to NASH. In December 2019, we submitted a
Marketing  Authorization  Application  (“MAA”)  to  the  European  Medicines  Agency  (the  “EMA”)  seeking  conditional
approval of OCA for liver fibrosis due to NASH. In January 2020, the EMA validated our MAA and thereby confirmed
that  our  MAA  was  sufficiently  complete  to  begin  the  formal  review  process.  In  June  2020,  we  received  a  complete
response letter (“CRL”) from the FDA stating that our NDA for OCA for the treatment of liver fibrosis due to NASH could
not  be  approved  in  its  present  form.  The  CRL  indicated  that,  based  on  the  data  the  FDA  had  reviewed,  the  FDA  has
determined that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not
sufficiently outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due
to  NASH.  At  that  time,  the  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data
from the ongoing REGENERATE trial in support of potential accelerated approval and that the long-term outcomes phase
of the trial should continue. We are in discussions with the FDA with respect to the potential resubmission of our NDA
seeking accelerated approval of OCA for the treatment of liver fibrosis due to NASH. We had our end of review meeting
with the FDA in October 2020 to discuss the FDA’s risk-benefit assessment in the CRL based on its review of the available
data, as well as our proposed resubmission of our NDA for the treatment of liver fibrosis due to NASH. The meeting was

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constructive  and  the  FDA  has  provided  us  with  helpful  guidance  regarding  supplemental  data  we  can  provide  to  further
characterize OCA’s efficacy and safety profile that could support resubmission based on our Phase 3 REGENERATE 18-
month biopsy data, together with a safety update from our ongoing studies. We are advancing accordingly and plan to hold
additional meetings with the FDA with the goal of achieving sufficient alignment to proceed on this basis and potentially
resubmit our NDA for the treatment of liver fibrosis due to NASH by the end of 2021. In addition, we continue to work
collaboratively with the EMA on its review of our MAA.

As part of our product development activities, we expect to continue to invest in evaluating the potential of OCA in
progressive  non-viral  liver  diseases.  We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with
compensated cirrhosis, known as the REVERSE trial. In January 2020, we announced that we completed enrollment of the
REVERSE  trial  with  over  900  patients  randomized.  We  are  also  studying  OCA  in  combination  with  bezafibrate,  a  pan-
peroxisome  proliferator-activated  receptor  agonist,  in  patients  with  PBC  and  potentially  may  study  such  combination  in
other liver diseases. In addition, we have other compounds in early stages of research and development in our pipeline.

Liver Function, Bile Acids and Progressive Non-Viral Liver Diseases

The  liver  performs  many  functions  that  are  vital  for  maintaining  health,  including  the  regulation  of  bile  acid
metabolism. Bile acids are natural detergent-like emulsifying agents that are released from the gallbladder into the intestine
when food is ingested, and are essential for the absorption of dietary cholesterol and other nutrients. Cholesterol bound by
bile acids is taken up by the liver, where the cholesterol is then converted into one of two primary bile acids. The bile acids
are  then  actively  secreted  into  bile  ducts,  which  eventually  empty  into  the  gallbladder.  This  digestive  cycle  of  bile  flow
from gallbladder to intestine to liver and back is called the enterohepatic recirculation of bile.

In  addition  to  facilitating  nutrient  absorption,  bile  acids  act  as  important  signals  that  help  regulate  multiple  other
biological functions. They are also complex signaling molecules that integrate metabolic and immune pathways involved in
the  healthy  functioning  of  various  tissues  and  organs.  For  example,  the  actions  of  bile  acids  in  the  liver,  intestine  and
kidney regulate repair mechanisms that modulate inflammation and fibrosis (scarring), which can lead to progressive organ
damage.

The biological effects of bile acids are mediated through dedicated receptors. The best understood receptor is FXR, a
nuclear receptor that regulates bile acid synthesis and clearance from the liver, thereby preventing excessive bile acid build-
up in the liver, which may be toxic. As such, FXR is a target for the treatment of several liver diseases such as PBC that
involve  impaired  bile  flow,  a  condition  called  cholestasis.  In  cholestasis,  the  liver  is  typically  exposed  to  higher  than
normal  levels  of  bile  acids,  which  can  cause  significant  damage  over  time.  In  addition,  bile  acid  activation  of  FXR  is
believed to induce anti-fibrotic, anti-inflammatory, anti-steatotic and other mechanisms that are necessary for the normal
regeneration of the liver. As a result, FXR is also a target for the treatment of more common liver diseases such as NASH
and alcoholic hepatitis. Further, based on the discovery of similar FXR-mediated protective mechanisms in other organs
exposed to bile acids, we believe that FXR may also be a potential target for the treatment of a number of intestinal, kidney
and other diseases.

OCA is a bile acid analog, a chemical substance that has a structure based on a naturally occurring human bile acid,
that selectively binds to and activates FXR. We believe that OCA has broad liver-protective properties and may effectively
counter a variety of chronic insults to the liver that cause fibrosis (scarring), which can eventually lead to cirrhosis, liver
transplant and death. Due to OCA’s bile acid-like properties, it circulates enterohepatically and engages FXR in both the
liver  and  intestine.  FXR  engagement  in  the  liver  is  believed  to  be  critical  to  successfully  treat  pathologic  injury  due  to
progressive underlying disease.

By  virtue  of  our  patent  portfolio  and  the  proprietary  know-how  of  our  employees  and  collaboration  partners,  we
believe that we hold a leading position in the fields of bile acid chemistry and therapeutics. Our research and development
efforts  have  resulted  in  a  pipeline  of  bile  acid  analogs  in  addition  to  OCA  and  through  our  on-going  work  with  our
collaboration partners such as Professor Roberto Pellicciari, Ph.D., one of our co-founders, and TES Pharma S.r.l., we are
continuing  our  research  to  rationally  design  compounds  that  bind  selectively  and  potently  to  FXR  and  other  bile  acid
receptors.

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Our Strategy

Our  objective  is  to  develop  and  commercialize  novel  therapeutics  for  the  treatment  of  progressive  non-viral  liver

diseases with high unmet medical need. The key elements of our strategy are to:

● Further  strengthen  our  foundational  PBC  business.  We  intend  to  further  strengthen  our  foundational  PBC
business through expanding access to Ocaliva to eligible patients by increasing Ocaliva’s penetration in the
markets  where  it  has  been  approved  and  pursuing  regulatory  approval  for  Ocaliva  in  our  target  markets
where  it  has  not  yet  been  approved.  In  addition,  we  continue  to  work  to  execute  on  our  post-marketing
regulatory commitments with respect to Ocaliva in the U.S. and Europe.

● Execute  on  our  clinical  and  regulatory  goals  and  timelines.  We  remain  focused  on  progressing  our
development  program  in  liver  fibrosis  due  to  NASH  in  the  United  States  and  Europe  and  are  working  to
potentially resubmit our NDA to the FDA by the end of 2021. We also expect to continue REGENERATE
through clinical outcomes and to progress our Phase 3 REVERSE trial for NASH patients with compensated
cirrhosis.  We  also  plan  to  advance  our  Phase  2  study  evaluating  bezafibrate  in  combination  with  OCA  for
PBC as part of a broader early development program.

● Expand our portfolio and pipeline. We intend to identify additional opportunities to develop OCA and our
other product candidates, alone or in combination, in rare liver diseases. In addition, we intend to initiate a
first-in-human  clinical  trial  of  our  INT-787  compound,  which  is  an  FXR  agonist  that  we  are  currently
evaluating in preclinical studies

● Expand and protect our intellectual property. We intend to continue to expand and aggressively prosecute our
intellectual property in the area of bile acid chemistry and therapeutics with the objective of maintaining a
valuable intellectual property portfolio and to vigorously defend and enforce our intellectual property rights
protecting Ocaliva.

History and Development of the Company

In  September  2002,  we  were  incorporated  in  Delaware  and  shortly  thereafter  began  operations  in  New  York.  In
October  2012,  following  several  rounds  of  private  funding,  we  completed  our  initial  public  offering  (the  “IPO”)  and
received net proceeds of approximately $78.7 million therefrom. We used the proceeds from our IPO to fund, among other
things, preclinical and clinical development activities, including our Phase 3 POISE trial studying OCA for PBC and work
performed in anticipation of our submission of regulatory filings for the approval of OCA for PBC. In addition, between
June 2013 and April 2015, we completed four registered public offerings of our common stock and received aggregate net
proceeds of approximately $803.4 million therefrom.

In  March  2014,  we  announced  the  results  of  our  Phase  3  POISE  trial  of  OCA  for  PBC.  In  November  2014,  results
from the FLINT Phase 2b clinical trial of OCA for liver fibrosis due to NASH were published in The Lancet. Both of these
trials met their primary endpoints.

In June 2015, we submitted a NDA to the FDA seeking accelerated approval of OCA for PBC and a MAA to the EMA
seeking  conditional  approval  of  OCA  for  PBC.  In  September  2015,  we  announced  the  initiation  of  our  Phase  3
REGENERATE trial of OCA in patients with liver fibrosis due to NASH.

In  May  2016,  Ocaliva  was  approved  for  PBC  by  the  FDA.  We  commenced  sales  and  marketing  of  Ocaliva  in  the
United States shortly after receiving approval. In July 2016, we issued and sold $460.0 million aggregate principal amount
of 3.25% Convertible Senior Notes due 2023 (the “2023 Convertible Notes”) in a registered public offering and received
net  proceeds  of  approximately  $447.6  million  therefrom.  In  December  2016,  Ocaliva  received  conditional  approval  for
PBC from the European Commission.

In  January  2017,  we  commenced  our  European  launch  of  Ocaliva  for  PBC.  Since  January  2017,  Ocaliva  has  also

received regulatory approval in several of our target markets outside the United States and Europe, including Canada,

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Israel and Australia, and we are pursuing marketing approval of Ocaliva for PBC in our other international target markets.
In July 2017, we announced positive results from our Phase 2 CONTROL trial, the goal of which was to characterize the
lipid metabolic effects of OCA and cholesterol management effects of concomitant statin administration in NASH patients,
as well as positive top-line results from our Phase 2 AESOP trial of OCA for primary sclerosing cholangitis (“PSC”).

In February 2018, we announced our Phase 3 REVERSE trial of OCA for liver fibrosis due to NASH patients with
compensated  cirrhosis.  In  April  2018,  we  issued  and  sold  an  aggregate  of  approximately  4.3  million  shares  of  common
stock in a registered public offering and a concurrent private placement (the “2018 Concurrent Private Placement”) exempt
from the registration requirements of the Securities Act of 1933, as amended, and received net proceeds of approximately
$261.4  million  therefrom.  In  December  2018,  we  entered  into  an  agreement  (the  “Aralez  Agreement”)  with  Aralez
Pharmaceuticals Canada Inc. (“Aralez”), pursuant to which we acquired (i) Aralez’s license to develop and commercialize
bezafibrate in the United States, (ii) Aralez’s investigational new drug application (“IND”) on file with the FDA and other
associated  regulatory  documentation  and  (iii)  a  non-exclusive  license  to  certain  of  Aralez’s  intellectual  property.  We  are
evaluating the efficacy, safety and tolerability of bezafibrate in combination with OCA in patients with PBC in a Phase 2
study, with the longer-term goal of developing and seeking regulatory approval for a fixed dose combination regimen in
this indication and potentially other liver diseases.

In February 2019, we announced topline results from our pivotal Phase 3 REGENERATE trial in patients with liver
fibrosis due to NASH. In the primary efficacy analysis, once-daily OCA 25 mg met the primary endpoint agreed with the
FDA of fibrosis improvement by at least one stage with no worsening of NASH at the planned 18-month analysis. Adverse
events were generally mild to moderate in severity and the most common were consistent with the known profile of OCA.

In May 2019, we issued and sold $230.0 million aggregate principal amount of 2.00% Convertible Senior Notes due
2026 (the “2026 Convertible Notes” and together with the 2023 Convertible Notes, the “Convertible Notes”) in a registered
public  offering  and  received  net  proceeds  of  approximately  $223.4  million  therefrom.  In  May  2019,  we  issued  and  sold
2,760,000  shares  of  common  stock  in  a  registered  public  offering  (“the  2019  Public  Offering”)  and  119,760  shares  of
common  stock  in  a  concurrent  private  placement  of  common  stock  (the  “2019  Concurrent  Private  Placement”)  and
received net proceeds of approximately $227.3 million.

In September 2019, we submitted a NDA to the FDA seeking accelerated approval of OCA for liver fibrosis due to
NASH. In November 2019, the FDA accepted our NDA for filing and granted a priority review designation for OCA for
liver fibrosis due to NASH. Under PDUFA, the FDA has set a target action date of June 26, 2020 for the completion of its
review of our NDA, after giving effect to a 90-day extension of its initial target action date. The FDA has also notified us
that it has tentatively scheduled an advisory committee meeting relating to our NDA for April 22, 2020.

In December 2019, we submitted a MAA to the EMA seeking conditional approval of OCA for liver fibrosis due to
NASH. In January 2020, the EMA validated our MAA and thereby confirmed that our MAA was sufficiently complete to
begin the formal review process.

In June 2020, we received a complete response letter (“CRL”) from the FDA stating that our NDA for OCA for the
treatment of liver fibrosis due to NASH could not be approved in its present form. The CRL indicated that, based on the
data  the  FDA  had  reviewed,  the  FDA  has  determined  that  the  predicted  benefit  of  OCA  based  on  a  surrogate
histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently  outweigh  the  potential  risks  to  support  accelerated
approval for the treatment of patients with liver fibrosis due to NASH. At that time, the FDA recommended that we submit
additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing  REGENERATE  trial  in  support  of  potential
accelerated approval and that the long-term outcomes phase of the trial should continue.

In October 2020, we had our end of review meeting with the FDA to discuss the FDA’s risk-benefit assessment in the
CRL based on its review of the available data, as well as our proposed resubmission of our NDA for the treatment of liver
fibrosis  due  to  NASH.  The  meeting  was  constructive  and  the  FDA  has  provided  us  with  helpful  guidance  regarding
supplemental data we can provide to further characterize OCA’s efficacy and safety profile that could support resubmission
based on our Phase 3 REGENERATE 18-month biopsy data, together with a safety update from our ongoing studies.

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In  December  2020,  we  announced  that  Mark  Pruzanski,  M.D.  would  retire  from  his  position  as  President  and
Chief  Executive  Officer  and  that  Jerome  (Jerry)  Durso,  our  Chief  Operating  Officer  at  the  time,  would  succeed  Dr.
Pruzanski as our President and Chief Executive Officer, effective as of January 1, 2021. We also announced that Mr. Durso
would be appointed to the Board of Directors (the “Board”) following the transition and that Dr. Pruzanski would remain as
a director on the Board and retained adviser to us.

For information regarding our financial condition and results of operations, including our revenues, net loss and total
assets,  see  our  audited  consolidated  financial  statements  and  accompanying  notes  and  “Management’s  Discussion  and
Analysis of Financial Condition and Results of Operations” included elsewhere in this Annual Report on Form 10-K.

Our First Approved Product  

Ocaliva

Ocaliva  was  approved  for  PBC  by  the  FDA  in  May  2016  under  the  accelerated  approval  pathway.  We  commenced
sales and marketing of Ocaliva in the United States shortly after receiving approval, and Ocaliva is now available to U.S.
patients  primarily  through  a  network  of  specialty  pharmacy  distributors.  Ocaliva  received  conditional  approval  for  PBC
from the European Commission in December 2016 and we commenced our European commercial launch in January 2017.
We have submitted dossiers and obtained, or are otherwise pursuing, reimbursement from a number of national authorities
in Europe. Since January 2017, Ocaliva has also received regulatory approval in several of our target markets outside the
United States and Europe, including Canada, Israel and Australia, and we are pursuing marketing approval of Ocaliva for
PBC in our other international target markets. Ocaliva received orphan drug designation in both the United States and the
European Union for the treatment of PBC.

Overview of PBC

PBC is a rare liver disease that primarily results from autoimmune destruction of the bile ducts that transport bile acids
out of the liver, resulting in cholestasis. The build-up of bile acids in the liver damages liver cells. These damaged liver
cells, in turn, release abnormal amounts of serum alkaline phosphatase (“ALP”), a liver enzyme that is a key biomarker of
the disease pathology. As shown in numerous clinical trials of treatment with UDCA (available generically as ursodiol), a
positive  therapeutic  response  is  primarily  determined  by  sustained  reduction  of  ALP  levels,  along  with  maintenance  of
normal bilirubin levels, indicating adequately compensated liver function. This biochemical improvement has been shown
to  correlate  well  with  improved  clinical  outcomes  such  as  transplant-free  survival.  As  the  disease  progresses,  it  causes
progressive  liver  damage  marked  by  chronic  inflammation  and  fibrosis.  Despite  its  rarity,  PBC  is  the  most  common
cholestatic  liver  disease  and  is  among  the  leading  indications  for  liver  transplant  among  women  in  the  United  States.
Disease  progression  in  PBC  varies  significantly,  with  median  survival  in  untreated  patients  estimated  to  be  7.5  years  if
symptomatic at diagnosis and up to 16 years if asymptomatic at diagnosis. PBC patients whose disease is progressing have
persistently  elevated  levels  of  ALP  and  other  liver  enzymes,  with  abnormal  bilirubin  levels  heralding  more  advanced
disease.  Data  from  published  long-term  studies  demonstrate  that  a  significant  portion  of  such  patients  with  advancing
disease progress to liver failure, transplant or death within five to ten years.

Based on our analysis of 2016 industry data, there were approximately 290,000 people with PBC at the time of our
U.S. launch in the United States, certain European countries, Canada, Australia and New Zealand. An estimated 90% of
PBC patients are women, with approximately one in 1,000 women over the age of 40 afflicted by the disease. The mean
age of diagnosis is about 40 years old and the typical initial presentation occurs between the ages of 30 and 65 years old. A
majority of PBC patients are asymptomatic at the time of initial diagnosis, but most develop symptoms over time. Fatigue
and pruritus are the most common symptoms in PBC patients. Less common symptoms include dry eyes and mouth, as
well as jaundice, which can be seen in more advanced disease. Based on the guidelines of the American Association for the
Study  of  Liver  Disease  and  the  European  Association  for  the  Study  of  the  Liver,  the  clinical  diagnosis  of  PBC  is
established  based  on  the  presence  of  (i)  a  positive  antimitochondrial  antibody  (“AMA”),  a  marker  of  this  autoimmune
disease seen in up to 95% of PBC patients and (ii) elevated serum levels of ALP. In the earlier stages of PBC, ALP is often
the  only  abnormally  elevated  liver  enzyme,  rising  to  between  two  to  ten  times  higher  than  normal  values.  Bilirubin  is  a
marker of liver function and is also monitored in PBC to provide an indication of how well the liver is

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functioning. Liver biopsy can be used to confirm the diagnosis of PBC, but is not required and is becoming less-frequently
performed.

A  number  of  published  clinical  studies  have  demonstrated  that  lower  levels  of  ALP,  both  independently  or  in
conjunction with normal bilirubin levels, correlate with a significant reduction in adverse clinical outcomes such as liver
transplant and/or death in PBC patients. These studies include the result of meta-analyses of PBC clinical outcomes data of
more than 6,000 PBC patients from 15 academic centers in eight countries that have been compiled by the Global PBC
Study Group, which we sponsored, as well as a dataset of over 6,000 PBC patients across the United Kingdom compiled by
the UK PBC Group.

Prior to Ocaliva, the only approved drug indicated for the treatment of PBC was UDCA, which is widely considered
the  standard  first-line  therapy  for  PBC  patients.  In  patients  for  whom  UDCA  is  effective,  the  treatment  slows  the
progression of PBC, reducing the likelihood of liver failure and the need for transplant.

Phase 3 POISE Trial

Ocaliva’s accelerated approval in the United States and conditional approval in the European Union was supported by
the results of our Phase 3 POISE trial, which was completed in March 2014. The data from the POISE trial showed that
Ocaliva, at both a once-daily 10 mg dose and a once-daily 5 mg dose titrated to 10 mg, met the trial’s primary endpoint of
achieving a reduction in ALP to below a threshold of 1.67 times the upper limit of normal (“ULN”), with a minimum of a
15%  reduction  in  ALP  level  from  baseline,  and  a  normal  bilirubin  level  after  12  months  of  therapy.  The  percentage  of
patients meeting the POISE trial’s primary endpoint was 10% in the placebo group, 47% in the 10 mg Ocaliva group and
46% in the Ocaliva titration group (both dose groups p < 0.0001 as compared to placebo) in an intent-to-treat analysis. The
placebo group experienced a mean decrease in ALP from baseline of 5%, compared to a mean decrease of 39% in the 10
mg  Ocaliva  dose  group  and  33%  in  the  Ocaliva  titration  group  (both  dose  groups  p  <  0.0001  as  compared  to  placebo).
Pruritus, generally mild to moderate, was the most frequently reported adverse event associated with Ocaliva treatment and
was  observed  in  38%  of  patients  on  placebo,  70%  of  patients  in  the  10  mg  Ocaliva  group  and  56%  of  patients  in  the
Ocaliva titration group. Eight patients discontinued due to pruritus, of whom none were in the placebo group, seven (10%)
were in the 10 mg Ocaliva group and one (1%) was in the Ocaliva titration group. Decreases in high density lipoprotein
(“HDL”) cholesterol were also observed during treatment.

Following  the  completion  of  the  double-blind  portion  of  the  POISE  trial  described  above,  patients  were  given  the
option to enroll in a five-year open-label long-term safety and efficacy extension trial, which has been completed. Patients
received Ocaliva at a once-daily 5 mg dose for three months, after which patients were titrated based on tolerability. The
data from the open-label extension portion of the trial showed that 46% of patients responded after 12 months of treatment
with Ocaliva and 50% to 56% of patients responded after 48 to 72 months of treatment with Ocaliva (based on the same
criteria used to define the primary endpoint in the 12 month placebo controlled trial). Reductions in ALP were sustained
through the double-blind and extension portions of the trial and total bilirubin levels remained stable and within the normal
range for most patients for the duration of the trial (ALP p < 0.0001 for all post-baseline visits; total bilirubin: p-values
were not consistently significant throughout the extension portion of the POISE trial). Adverse events were consistent with
the safety profile of Ocaliva in patients with PBC. The most commonly reported adverse events were pruritis and fatigue,
which were generally mild to moderate in severity.

Ongoing Confirmatory Clinical Outcomes Trial and Other Post Marketing Requirements

In  connection  with  Ocaliva’s  accelerated  approval  in  the  United  States  and  conditional  approval  in  the  European
Union, we committed to conduct a Phase 4 confirmatory outcomes trial of Ocaliva, known as the COBALT trial, and other
clinical  trials  to  satisfy  post-marketing  regulatory  requirements.  Continued  approval  of  Ocaliva  for  PBC  in  the  United
States, the European Union and other jurisdictions is contingent upon the verification and description of clinical benefit in
the COBALT trial and our satisfaction of our other post-marketing regulatory requirements. Any delay or failure by us to
satisfy  such  requirements,  including  any  delay  or  failure  relating  to  our  Phase  4  COBALT  trial,  may  jeopardize  the
continued approval of Ocaliva for PBC in the United States, European Union and other jurisdictions.

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The goal of the COBALT trial is to confirm that reduction of ALP based upon Ocaliva treatment is associated with a
longer-term benefit on liver-related clinical outcomes. COBALT is designed to assess the effect of a once-daily dose of 5
mg or 10 mg of Ocaliva in approximately 430 PBC patients with an inadequate therapeutic response to UDCA or who are
unable to tolerate UDCA. In this trial, eligible patients with PBC continue their UDCA treatment, except for those patients
unable  to  tolerate  UDCA,  have  been  randomized  into  one  of  two  treatment  arms  of  approximately  215  patients  each.
Patients have been randomized to receive either (i) placebo or (ii) Ocaliva starting at 5 mg and increasing over the course
of the trial to 10 mg of Ocaliva based on tolerability. Dosing frequency has been determined by disease stage. The primary
endpoint  of  the  trial  is  based  on  clinical  outcomes  as  measured  by  time  to  first  occurrence  of  any  of  the  following
adjudicated events: death (all-cause), liver transplant, Model of End Stage Liver Disease (“MELD”) score greater than 15,
uncontrolled ascites or hospitalization due to variceal bleeding, hepatic encephalopathy or spontaneous bacterial peritonitis.
The study evaluates subjects across the spectrum of PBC disease, including early and advanced PBC.

Further, as part of our post-marketing requirements for Ocaliva, we are undertaking a Phase 4 clinical trial of Ocaliva
in patients with PBC who have moderate to severe hepatic impairment (Child-Pugh B and C) (known as the 401 trial). This
double-blind, placebo-controlled study is designed to evaluate the pharmacokinetics of Ocaliva and its conjugates, as well
as safety and tolerability. Additional objectives include an evaluation of Ocaliva treatment compared to placebo on liver
biochemistry, Child-Pugh scores and non-invasive markers of liver fibrosis and stiffness. The trial as designed is targeted to
enroll approximately 50 patients in the United States, Europe and other jurisdictions for 48 weeks.

While we remain blinded to safety and efficacy data in the ongoing COBALT trial and 401 trial, a data monitoring
committee (“DMC”) reviewed the unblinded results of a pre-specified interim efficacy analysis of the COBALT trial and
separately  reviewed  unblinded  safety  and  pharmacokinetic  data  from  both  the  COBALT  and  401  trials.  Following  these
reviews,  the  DMC  stated  that  it  was  not  feasible  to  continue  the  COBALT  trial  as  designed  and  noted  the  challenges  in
enrolling and maintaining placebo-controlled post-marketing studies in this rare disease setting. No acute safety concerns
were noted by the DMC. Given the feasibility concerns noted by the DMC as well as the potential confounding impact of
subjects discontinuing treatment and/or transitioning from investigational product to commercial drug during clinical trials,
we continue to discuss with the FDA and the EMA proposed modifications to the COBALT trial as well as proposals with
respect to the 401 trial. We have notified the FDA and the EMA of the DMC’s recommendation and, as they previously
advised, are in ongoing discussions with the FDA on the matter and are seeking formal EU scientific advice with respect to
potential  alternative  study  designs.  In  addition,  future  changes  to  our  Ocaliva  label  related  to  the  most  advanced  PBC
patients  will  influence  the  modifications  to  our  study  design.  Both  the  COBALT  and  401  trials  are  ongoing  but  not
currently enrolling patients.

We are also undertaking a Phase 2 clinical trial of Ocaliva in pediatric patients with biliary atresia, a life-threatening
condition in infants in which the bile ducts inside or outside the liver do not have normal openings. This trial, known as the
CARE  trial,  is  a  part  of  an  EMA-approved  Pediatric  Investigation  Plan  (“PIP”)  supporting  the  conditional  approval  of
Ocaliva  for  PBC  in  the  European  Union  as  PBC  is  not  believed  to  occur  in  the  pediatric  population.  The  CARE  trial  is
designed  to  evaluate  the  effects  of  11  weeks  of  Ocaliva  treatment  where  patients  with  biliary  atresia  are  randomized  to
varying  doses.  The  primary  endpoint  is  to  evaluate  the  pharmacokinetics  and  the  safety  and  tolerability  of  Ocaliva
treatment. In addition, Ocaliva’s effect on hepatobiliary indices and biomarkers will be assessed. This trial is targeted to
enroll approximately 60 patients in the United States and Europe.

Ocaliva Label Update

In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended  weekly  dose  in  such  patients.  As  a  result,  in  September  2017,  we  issued  a  Dear  Health  Care  Provider
(“DHCP”)  letter,  and  the  FDA  also  subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended
label dosing. Both communications remind healthcare providers of the importance of the recommended reduced dosing of
Ocaliva in PBC patients with moderate or severe hepatic impairment, while reiterating the importance of monitoring PBC
patients  for  progression  of  their  disease  and  the  occurrence  of  liver-related  adverse  reactions.  In  addition  to  the  DHCP
letter,  we  took  actions  to  enhance  education  about  appropriate  use  of  Ocaliva.  These  initiatives  included:  reeducating
physicians on the label, with a focus on ensuring appropriate dosing for patients with moderate or severe hepatic

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impairment; enhancing monitoring of patients for liver-related adverse reactions; and adjudicating reported cases of serious
liver injury, including in patients with no or mild hepatic impairment.

In February 2018, we announced that the Ocaliva label in the United States had been updated by the FDA to include a
boxed warning and a dosing table that reinforced the then-existing dosing schedule for patients with Child-Pugh Class B or
C  or  decompensated  cirrhosis.  In  addition,  the  FDA  issued  an  updated  drug  safety  communication  to  accompany  the
revised  label.  We  remain  focused  on  the  safety  of  all  of  the  patients  using  Ocaliva  within  and  outside  of  our  ongoing
clinical studies and have engaged with relevant regulatory authorities to ensure that the Ocaliva label sufficiently reinforces
the importance of appropriate dosing in patients with advanced cirrhosis.

The FDA has notified us that, in the course of its routine safety surveillance, in May 2020 the FDA began to evaluate a
newly identified safety signal, or NISS, regarding liver disorder for Ocaliva which the FDA classified as a potential risk.
The  FDA  has  informed  us  that  its  review  of  the  NISS  is  focused  on  a  subset  of  the  cirrhotic,  or  more  advanced,  PBC
patients who have taken Ocaliva. As part of our routine pharmacovigilance efforts, we worked with the FDA to reconcile
our internal safety database with the FDA Adverse Event Reporting System database and we completed a comprehensive
assessment of all available data, including data from our completed clinical trials, blinded reviews of ongoing clinical trial
data,  unblinded  reviews  of  certain  ongoing  clinical  trial  data  by  the  DMC,  post-marketing  data  and  natural  history  data,
which we submitted to the FDA and had a meeting earlier in 2021 to discuss. We are working with the FDA to align on
changes to the Ocaliva label regarding patients with the most advanced stages of PBC. Based on our communications with
the FDA, this update will come in the form of a safety labeling change. These communications are ongoing.

Our Product Candidates

The following summarizes the current status and the anticipated next steps in our development plans for our product
candidates.  We  continually  evaluate  each  product  candidate  in  an  effort  to  efficiently  allocate  research  and  development
funds to projects we deem to be in our best interests based on, among other factors, the product candidate’s performance in
pre-clinical  and/or  clinical  studies,  our  expectations  regarding  the  potential  future  regulatory  approval  of  the  product
candidate and our view of the potential commercial viability of the product candidate in light of market conditions.

OCA for liver fibrosis due to NASH

Our lead product candidate is OCA for the potential treatment of liver fibrosis due to NASH. In February 2019, we
announced  topline  results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in
patients with liver fibrosis due to NASH, known as the REGENERATE trial. In the primary efficacy analysis, once-daily
OCA  25  mg  met  the  primary  endpoint  agreed  with  the  FDA  of  fibrosis  improvement  by  at  least  one  stage  with  no
worsening of NASH at the planned 18-month interim analysis. Adverse events were generally mild to moderate in severity
and  the  most  common  were  consistent  with  the  known  profile  of  OCA.  OCA  has  received  breakthrough  therapy
designation from the FDA for the treatment of NASH patients with liver fibrosis. In September 2019, we submitted a NDA
seeking  accelerated  approval  of  OCA  for  liver  fibrosis  due  to  NASH  in  the  United  States  and,  in  December  2019,  we
submitted a MAA seeking conditional approval of OCA for liver fibrosis due to NASH in Europe. The FDA subsequently
accepted our NDA for filing and granted a priority review designation for OCA for liver fibrosis due to NASH. In January
2020, the EMA validated our MAA and thereby confirmed that our MAA was sufficiently complete to begin the formal
review  process.  In  June  2020,  we  received  a  complete  response  letter  (“CRL”)  from  the  FDA  stating  that  our  NDA  for
OCA for the treatment of liver fibrosis due to NASH could not be approved in its present form. The CRL indicated that,
based on the data the FDA had reviewed, the FDA has determined that the predicted benefit of OCA based on a surrogate
histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently  outweigh  the  potential  risks  to  support  accelerated
approval for the treatment of patients with liver fibrosis due to NASH. At that time, the FDA recommended that we submit
additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing  REGENERATE  trial  in  support  of  potential
accelerated approval and that the long-term outcomes phase of the trial should continue. In October 2020, we had our end
of  review  meeting  with  the  FDA  to  discuss  the  FDA’s  risk-benefit  assessment  in  the  CRL  based  on  its  review  of  the
available  data,  as  well  as  our  proposed  resubmission  of  our  NDA  for  the  treatment  of  liver  fibrosis  due  to  NASH.  The
meeting was constructive and the FDA has provided us with helpful guidance regarding supplemental data we can provide
to  further  characterize  OCA’s  efficacy  and  safety  profile  that  could  support  resubmission  based  on  our  Phase  3
REGENERATE 18-month biopsy data, together with a safety update from our ongoing studies. We are advancing

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accordingly and plan to hold additional meetings with the FDA with the goal of achieving sufficient alignment to proceed
on this basis and potentially resubmit our NDA for the treatment of liver fibrosis due to NASH by the end of 2021. We also
continue to work collaboratively with the EMA on its review of our MAA. In addition, we have conducted a number of
other trials and studies in connection with our NASH development program, and our Phase 3 trial in NASH patients with
compensated cirrhosis, known as the REVERSE trial, is ongoing.

Overview of NASH

NASH is a serious progressive liver disease caused by excessive fat accumulation in the liver (steatosis) that induces
chronic  inflammation,  resulting  in  progressive  fibrosis  (scarring)  that  can  lead  to  cirrhosis,  eventual  liver  failure,  cancer
and death. More than 20% of patients with NASH are estimated to progress to cirrhosis within a decade of diagnosis and,
compared  to  the  general  population,  have  a  ten-fold  greater  risk  of  liver-related  mortality.  The  proportion  of  liver
transplants attributable to NASH has increased rapidly in recent years with NASH currently the second leading cause of
liver transplantation in the United States and, in females, the leading cause. NASH is anticipated to become the leading
indication  for  liver  transplantation  in  Europe  within  the  next  decade.  Additionally,  NASH  is  now  considered  to  be  the
leading, and a rapidly increasing, cause of hepatocellular carcinoma (primary liver cancer), of which up to 40% of cases in
NASH patients develop prior to developing cirrhosis.

Although  difficult  to  precisely  estimate,  epidemiology  research  estimates  that  the  global  prevalence  of  NASH  is
approximately  3  –  5%  and  is  expected  to  increase  markedly  by  2030.  Fibrosis  is  the  most  robust  predictor  of  long-term
overall mortality, liver transplantation and liver-related events in patients with NASH and advanced fibrosis is associated
with a substantially higher risk of liver-related morbidity and mortality in patients with NASH. We believe that a majority
of  NASH  patients  diagnosed  and  under  specialist  care  have  fibrosis  of  stage  2  or  greater.  Although  the  prevalence  of
NASH  is  lower  in  children,  it  has  also  become  a  serious  disease  burden  in  the  pediatric  population.  Other  common  co-
existing conditions such as obesity and type 2 diabetes, which are present in a majority of NASH patients, raise important
risks. NASH has been linked in both developed and developing countries to the adoption of a Western diet, with increased
consumption of processed foods containing polyunsaturated fatty acids and fructose.

Generally  in  clinical  trials  in  NASH,  a  definitive  diagnosis  requires  a  histologic  assessment  of  a  liver  biopsy  for
several key features associated with NASH, including, but not limited to, steatosis, lobular inflammation and hepatocyte
ballooning. However, we believe that the majority of NASH patients currently under treater care have been assessed for
liver  fibrosis  without  a  liver  biopsy.  Several  imaging  and  circulating  biomarkers  are  being  investigated  as  non-invasive
diagnostic methods, including transient elastography (an ultrasound technology approved in the United States and Europe
for the measurement of liver fibrosis), magnetic resonance imaging and serum biomarkers. NASH diagnosis rates in the
United States and the EU5 countries are very low, owing to a lack of approved treatment options and a lack of validated
non-invasive  diagnosis  options.  We  believe  the  availability  of  novel  therapeutics  and  non-invasive  technologies  will  be
instrumental in improving diagnosis rates.

There  are  currently  no  medications  approved  for  the  treatment  of  NASH  in  the  United  States  or  Europe.  However,
various  therapeutics  are  used  “off-label”,  such  as  vitamin  E  (an  antioxidant),  insulin  sensitizers  (e.g.,  metformin,
pioglitazone),  pentoxifylline  and  UDCA.  Lifestyle  changes,  including  modification  of  diet  and  exercise  to  reduce  body
weight, as well as treatment of concomitant diabetes and dyslipidemia, are commonly accepted as the standard of care, but
have  not  conclusively  been  shown  to  prevent  disease  progression.  Although  some  of  the  off-label  treatments  described
above have been studied as possible treatments for NASH, none has been approved by the FDA or EMA as a treatment for
this disease. Currently, treatment options for NASH patients with advanced cirrhosis are limited. Although liver transplant
can  be  life-saving,  many  patients  fail  to  receive  a  donor  organ  in  time,  and  for  those  who  do,  there  are  very  significant
clinical risks, such as infection and organ rejection, as well as significant costs. In addition, the post-transplant recurrence
rate of NASH has been shown to be as high as 25% at 18 months. Given the lack of available treatment options, we believe
that there is a significant unmet need for novel therapies for NASH, particularly in those patients with advanced fibrosis
and cirrhosis and those with a high risk of disease progression due to other co-morbidities such as type 2 diabetes.

FXR  activation  has  been  shown  to  play  a  key  role  in  the  regulation  of  the  metabolic  pathways  relevant  to  NASH,
highlighting  FXR  as  a  potential  drug  target  for  treatment  of  the  disease.  Given  the  significant  unmet  medical  need  of
patients with NASH, we believe that the ability of OCA to potently activate FXR has the potential to convey clinical

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benefit by improving key histologic parameters of the disease. This is supported by our preclinical and clinical results to
date, and is being further investigated in our ongoing clinical trial program.

Phase 3 REGENERATE Trial

We are currently conducting a pivotal Phase 3 clinical trial of OCA in patients with liver fibrosis due to NASH, known
as the REGENERATE trial. REGENERATE is a randomized, double-blind, placebo-controlled, multicenter study assessing
the safety and efficacy of OCA on liver-related clinical outcomes in patients with liver fibrosis due to NASH. Patients with
biopsy proven NASH with fibrosis are randomized 1:1:1 to receive placebo, OCA 10 mg or OCA 25 mg once daily. In
August  2019,  we  announced  the  completion  of  the  enrollment  of  the  clinical  outcomes  cohort  of  REGENERATE,  with
2,480  adult  NASH  patients  with  fibrosis  randomized  at  over  300  qualified  centers  worldwide.  REGENERATE  will
continue  through  clinical  outcomes  for  verification  and  description  of  clinical  benefit.  The  end-of-study  analysis  will
evaluate the effect of OCA on all-cause mortality and liver-related clinical outcomes.

An  18-month  interim  analysis  was  conducted  to  assess  the  effect  of  OCA  in  liver  histology  comparing  month  18
biopsy  with  baseline.  Patients  without  a  repeat  biopsy  due  to  study  discontinuation  or  other  reason  were  treated  as  non-
responders  in  the  primary  efficacy  analysis  and  full  efficacy  analysis  (each  as  described  below).  A  smaller  exploratory
cohort of patients with stage 1 liver fibrosis and at least one accompanying comorbidity (specified as diabetes, obesity or
alanine transaminase (“ALT”) greater than 1.5 times ULN) were also enrolled in REGENERATE, but were not included in
the  primary  efficacy  analysis.  As  described  below,  these  patients  were  included  in  the  full  efficacy  analysis  and  safety
analysis.  The  end-of-study  analysis  will  evaluate  the  effect  of  OCA  on  all-cause  mortality  and  liver-related  clinical
outcomes.

In February 2019, we announced topline results from the REGENERATE trial. In the primary efficacy analysis, once-
daily OCA 25 mg met, with statistical significance, the primary endpoint agreed with the FDA of fibrosis improvement by
at  least  one  stage  with  no  worsening  of  NASH  (defined  as  no  worsening  of  hepatocellular  ballooning,  no  worsening  of
lobular inflammation and no worsening of steatosis) at the planned 18-month analysis and adverse events were generally
mild  to  moderate  in  severity  and  the  most  common  were  consistent  with  the  known  profile  of  OCA.  Although  a
numerically greater proportion of patients in both OCA treatment arms compared to placebo achieved the primary endpoint
of NASH resolution with no worsening of liver fibrosis in the primary efficacy analysis, this result did not reach statistical
significance.  NASH  resolution  is  defined  as  the  overall  histopathologic  interpretation  of  (i)  no  fatty  liver  disease  or  (ii)
fatty liver disease (simple or isolated steatosis) without steatohepatitis AND a nonalcoholic fatty liver disease (“NAFLD”)
activity score (“NAS”) of 0 for ballooning and 0-1 for inflammation. As agreed with the FDA, in order for the primary
objective to be met, the study was required to achieve one of the two primary endpoints. In November 2019, the results of
the 18-month interim analysis from the REGENERATE trial were published in The Lancet.

The “primary efficacy analysis” (Intent-to-Treat or “ITT”) assessed efficacy at 18 months in 931 patients with stage 2
or 3 liver fibrosis due to NASH. Overall study discontinuations in the primary efficacy analysis population were balanced
across  treatment  arms:  16%  in  placebo,  17%  in  OCA  10  mg  and  15%  in  OCA  25  mg.  An  additional  pre-specified  “full
efficacy  analysis”  at  18  months  added  an  exploratory  cohort  of  287  NASH  patients  with  stage  1  liver  fibrosis  and
additional risk factors who were at increased risk of progression to cirrhosis (N = 1,218).

Set forth below is a summary of the 18-month primary efficacy analysis and additional full efficacy analysis from the

REGENERATE trial.

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Fibrosis Improvement at Month 18

Primary Efficacy Analysis 
(ITT population: NASH with stage 2 and 3 liver fibrosis)

Placebo
n = 311

OCA 10 mg
n = 312

OCA 25 mg
n= 308

Fibrosis improvement (≥ 1 stage) with no worsening of NASH*

Additional Full Efficacy Analysis  
     (ITT population plus stage 1 liver fibrosis patients)
Fibrosis improvement (≥ 1 stage) with no worsening of NASH*

11.9%

Placebo 
n=407
10.6%

17.6%
p = 0.0446
OCA 10 mg
n = 407
15.7%
p = 0.0286

23.1%
p = 0.0002**
OCA 25 mg
n = 404
21%
p < 0.0001

*    Defined as no worsening of hepatocellular ballooning, no worsening of lobular inflammation and no worsening of 
steatosis.
** Statistically significant in accordance with the statistical analysis plan agreed with the FDA.

NASH Resolution at Month 18

Primary Efficacy Analysis
(ITT population: NASH with stage 2 and 3 liver fibrosis
NASH resolution‡ with no worsening of liver fibrosis stage

Additional Full Efficacy Analysis
    (ITT population plus stage 1 liver fibrosis patients)
NASH resolution‡ with no worsening of liver fibrosis stage

Placebo
n = 311
8.0%

Placebo
n = 407
7.9%

OCA 10 mg
n = 312
11.2%
p = 0.1814
OCA 10 mg
n = 407
11.3%
p = 0.0903

OCA 25 mg
n = 308
11.7%
p = 0.1268
OCA 25 mg
n = 404
14.9%
p = 0.0013

‡ Defined as the overall histopathologic interpretation of (i) no fatty liver disease or (ii) fatty liver disease (simple or
isolated steatosis) without steatohepatitis AND a NAS of 0 for ballooning and 0-1 for inflammation.

The “safety population” in the planned 18-month analysis of REGENERATE included 1,968 randomized patients who

received at least one dose of investigational product (OCA or placebo).

Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most  common  were  consistent  with  the  known
profile of OCA. The frequency of serious adverse events was similar across treatment arms (11% in placebo, 11% in OCA
10 mg and 14% in OCA 25 mg) and no serious adverse event occurred in > 1% of patients in any treatment arm. There
were  3  deaths  (2  in  placebo:  bone  cancer  and  cardiac  arrest,  1  in  OCA  25  mg:  glioblastoma)  and  none  were  considered
related to treatment.

The most common adverse event reported was dose-related pruritus (19% in placebo, 28% in OCA 10 mg and 51% in
OCA  25  mg).  The  large  majority  of  pruritus  events  were  mild  to  moderate,  with  severe  pruritus  occurring  in  a  small
number  of  patients  (<  1%  in  placebo,  <  1%  in  OCA  10  mg  and  5%  in  OCA  25  mg).  A  higher  incidence  of  pruritus
associated treatment discontinuation was observed for OCA 25 mg (< 1% in placebo, < 1% in OCA 10 mg and 9% in OCA
25 mg). According to the clinical study protocol, investigator assessed severe pruritus mandated treatment discontinuation.

Consistent  with  observations  from  previous  NASH  studies,  OCA  treatment  was  associated  with  an  increase  in  low
density lipoprotein (“LDL”) cholesterol, with a peak increase of 22.6 mg/dL at four weeks and subsequently reversing and
approaching  baseline  at  month  18  (4.0  mg/dL  increase  from  baseline).  Statin  therapy  was  initiated  in  10%  of  placebo
patients  and  24%  of  each  OCA  treatment  arm.  Among  OCA  patients  who  initiated  statins,  LDL  cholesterol  increases
reversed  and  fell  to  below  baseline  levels  by  month  6.  Triglycerides  rapidly  and  continually  decreased  in  the  OCA
treatment arms through month 18. There were few and varied serious cardiovascular events and incidence was balanced
across the three treatment arms (2% in placebo, 1% in OCA 10 mg and 2% in OCA 25 mg).

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In patients with type 2 diabetes, OCA treatment was associated with an early transient increase in fasting glucose and
hemoglobin A1c with return to levels similar to placebo by month 6. No clinically meaningful changes were noted in non-
diabetic patients.

With  respect  to  hepatobiliary  events,  more  patients  (3%)  on  OCA  25  mg  experienced  gallstones  or  cholecystitis
compared to < 1% on placebo and 1% on OCA 10 mg. While numerically higher in the OCA 25 mg treatment arm, serious
hepatic adverse events were uncommon with < 1% incidence in each of the three treatment arms.

Phase 3 REVERSE Trial

We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with  compensated  cirrhosis,  known  as  the
REVERSE trial. REVERSE is a randomized, double-blind, placebo-controlled, multicenter trial evaluating the safety and
efficacy  of  OCA  in  NASH  patients  with  compensated  cirrhosis.  In  January  2020,  we  announced  that  we  completed
enrollment  of  the  REVERSE  trial  with  over  900  patients  with  a  biopsy-confirmed  diagnosis  of  cirrhosis  due  to  NASH
randomized.

The primary endpoint for REVERSE is the percentage of subjects with histological improvement in fibrosis by at least
one  stage  with  no  worsening  of  NASH  using  the  NASH  Clinical  Research  Network  scoring  system  after  18  months  of
treatment. Patients are randomized 1:1:1 into one of three treatment arms receiving a once-daily dose of placebo, OCA 10
mg or OCA 10 mg for the first three months with titration in accordance with the study protocol up to OCA 25 mg for the
remaining study period. Patients who successfully complete the double-blind phase of REVERSE will be eligible to enroll
in an open-label extension phase for up to 12 additional months.

Phase 2 CONTROL Trial

In  December  2015,  we  initiated  a  Phase  2  clinical  trial,  known  as  the  CONTROL  trial,  to  characterize  the  lipid
metabolic  effects  of  OCA  and  cholesterol  management  effects  of  concomitant  statin  administration  in  NASH  patients.
CONTROL enrolled approximately 80 NASH patients who were naïve to statin therapy or had undergone a statin washout
period. Statin-naïve or washout patients were randomized to receive one of three doses of OCA (5 mg, 10 mg or 25 mg) or
placebo. The study included a 16-week double-blind phase followed by an optional long-term safety extension (“LTSE”).

In July 2017, we announced that CONTROL met its primary objective by showing that newly initiated treatment with
atorvastatin rapidly reversed OCA-associated increases in LDL cholesterol to below baseline levels. Most of the effect was
observed  four  weeks  after  initiation  of  the  lowest  available  dose  of  atorvastatin  and  was  sustained  throughout  the  study
period. OCA treatment in the absence of statin therapy over the first four weeks resulted in an increase in LDL cholesterol
across all OCA treatment groups, while the placebo group was relatively unchanged. Treatment with atorvastatin beginning
at week four and continuing through week 16 reversed OCA-related increases in LDL cholesterol to below baseline levels
in all OCA treatment groups. Dose-dependent pruritus was the most common adverse event in patients treated with OCA,
occurring in 5% of patients on placebo, 5% of patients in the OCA 5 mg group, 10% of patients in the OCA 10 mg group
and 55% of patients in the OCA 25 mg group. All adverse events were mild to moderate and two patients discontinued
treatment  in  the  OCA  25  mg  group  due  to  pruritus.  Over  95%  of  the  patients  completing  the  double-blind  phase  of
CONTROL enrolled in the LTSE phase of the trial. During the LTSE phase of CONTROL, there was one patient death,
which the principal investigator determined was unlikely related to OCA.

Phase 2 Sumitomo Dainippon Trial

In October 2015, we announced the results of a 72-week Phase 2 dose ranging trial of OCA in 200 adult patients with
NASH in Japan. The trial was conducted by our former collaborator, Sumitomo Dainippon Pharma Co., Ltd. (“Sumitomo
Dainippon”). In this trial, 202 Japanese biopsy-proven NASH patients (NAS of 5-8) were randomized into one of four arms
to  receive  either  a  10  mg,  20  mg  or  40  mg  dose  of  OCA  or  placebo,  and  200  of  these  patients  (50  per  group)  initiated
treatment for a 72-week double-blind treatment phase, followed by a 24-week off treatment phase. The primary endpoint
was histologic improvement defined as at least a two-point improvement in NAS with no worsening of fibrosis.

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The primary efficacy analysis was conducted on an ITT basis, testing the dose dependent effects of once daily OCA
(10 mg, 20 mg and 40 mg) versus placebo on the primary endpoint. The ITT analysis included all randomized patients who
received  treatment  (50  per  group),  and  patients  who  discontinued  or  did  not  have  a  repeat  biopsy  were  treated  as  non-
responders.  A  pre-specified  completer  analysis  was  conducted  on  the  patients  who  had  biopsies  at  both  baseline  and  72
weeks (45, 44, 44 and 37 patients in the placebo, OCA 10 mg, OCA 20 mg and OCA 40 mg groups, respectively).

The  Sumitomo  Dainippon  trial  did  not  meet  statistical  significance  for  the  primary  endpoint.  The  ITT  results  in  the
table below show a dose dependent increase in the percentage of OCA-treated patients compared to placebo who achieved
the  primary  endpoint  (p  =  0.053).  Dose-dependent  trends  not  reaching  statistical  significance  were  observed  for  several
other pre-specified histologic endpoints, including the percentage of patients with steatosis and inflammation improvement,
ballooning resolution and NASH resolution. No difference was seen in fibrosis improvement in the OCA groups compared
to placebo.

ITT Results
NAS improvement > 2 points with
   no worsening of fibrosis

Placebo
N = 50
10 (20%)  

OCA 10 mg
N = 50
11 (22%)
p = 0.8070** 

OCA 20 mg
N = 50
14 (28%)
p = 0.3378** 

OCA 40 mg
N = 50
19 (38%)
p = 0.0496** 

p = 0.053*

*            Primary  efficacy  analysis  is  a  stratified  Cochran-Armitage  test  with  multiple  contrast  coefficients.  Statistical

significance is based on a p-value < 0.05.

**    The secondary efficacy analysis is a Cochran-Mantel-Haenszel (“CMH”) test stratified by baseline fibrosis stage for

Pairwise comparison of each OCA group compared to the placebo group. The multiplicity was not adjusted.

In the completer analysis, similar dose dependent effects were observed, with 51% of patients in the OCA 40 mg dose

group compared to 22% in the placebo group meeting the primary endpoint (p = 0.0061).

With the exception of dose dependent pruritus, OCA appeared to be generally safe and well tolerated. The number of
pruritus associated discontinuations were 0, 0, 2 and 5 patients in the placebo, OCA 10 mg, OCA 20 mg and OCA 40 mg
groups, respectively. Changes in lipid parameters, including LDL cholesterol, HDL cholesterol and triglycerides, appeared
to be consistent with previously reported lipid changes in Western NASH patients. No other meaningful differences in the
rate of adverse events between the OCA and placebo groups were noted.

Phase 2b FLINT Trial

In November 2014, the results from a Phase 2b clinical trial for the treatment of NASH, known as the FLINT trial,
which was sponsored by the NIDDK, a part of the National Institutes of Health, were published in The Lancet. The FLINT
trial was a double-blind, placebo-controlled trial of a once-daily dose of OCA 25 mg or placebo given for 72 weeks in 283
patients  with  biopsy-proven  NASH.  OCA  achieved  the  primary  endpoint  in  the  FLINT  trial,  which  was  defined  as  an
improvement of two or more points in NAS with no worsening of liver fibrosis.

The percentage of patients meeting the primary histological endpoint, based on liver biopsies, in the FLINT trial was
45% in the OCA treatment group and 21% in the placebo group (p = 0.0002, n = 219). The mean pre-treatment baseline
NAS for patients in the OCA treatment group was 5.3 of a total possible score of eight (comprised of a NAS of 0-2 for
hepatocellular  ballooning,  0-3  for  lobular  inflammation  and  0-3  for  steatosis).  Subgroup  analyses  showed  significant
response rates in the OCA treatment group in patients with risk factors for disease progression, including baseline fibrosis
stage,  co-morbid  type  2  diabetes  mellitus,  ALT,  insulin  resistance  and  severe  obesity  (each  factor  p  <  0.05  for  OCA
compared to placebo based on 95% confidence interval of published odds ratios).

A  significantly  greater  number  of  OCA-treated  patients  also  achieved  the  secondary  endpoint  of  improvement  of  at
least one fibrosis stage (35% versus 19%, p = 0.004), with OCA showing greater response rates as compared to placebo
across all stages of fibrosis. Based on our retrospective analyses of the FLINT data, more OCA-treated patients exhibited
fibrosis improvement of at least two fibrosis stages (15% versus 6%, not significant) and exhibited fibrosis improvements
regardless of baseline fibrosis stage and a significantly greater number of OCA-treated patients also achieved complete

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resolution of fibrosis (17% versus 5%, p = 0.0018). Also, our retrospective analysis of the FLINT data showed that fewer
OCA-treated patients progressed to bridging fibrosis (15% versus 18%, not significant) or to cirrhosis (2% versus 5%, not
significant). Retrospective analyses after the unblinding of results can potentially introduce bias and regulatory authorities
typically  give  greatest  weight  to  results  from  pre-specified  analyses  as  compared  to  retrospective  analyses.  The  NASH
Clinical  Research  Network  fibrosis  staging  system  was  used  to  categorize  the  pattern  of  fibrosis  and  architectural
remodeling  of  the  liver:  no  fibrosis  (F0),  perisinuoidal  or  periportal  fibrosis  (F1),  perisinusoidal  and  periportal  fibrosis
(F2), bridging fibrosis (F3) and cirrhosis (F4). Fibrosis sub-stages 1a, 1b and 1c were considered F1 for the analysis.

The  secondary  endpoint  of  NASH  resolution,  based  on  a  global  histological  assessment,  also  showed  improvement,
although  not  statistically  significant  (22%  versus  13%,  p  =  0.0832).  A  central  reading  of  all  baseline  and  end-of-trial
biopsies  was  performed  at  the  end  of  the  trial,  based  on  which  only  80%  of  patients  were  confirmed  to  have  definite
NASH,  while  the  remaining  20%  were  diagnosed  as  borderline  NASH  (10%)  or  not-NASH  (10%).  A  retrospective
subgroup  analysis  on  the  completer  population  comprised  only  of  definite  NASH  patients  at  baseline  showed  that  a
significantly  greater  number  of  OCA-treated  patients  achieved  NASH  resolution  compared  with  placebo-treated  patients
(19% versus 8%; p = 0.0278).

In an additional retrospective analysis of data from the FLINT trial conducted in a REGENERATE-matched patient
cohort published in 2018, (i) approximately 40% of OCA-treated patients as compared to approximately 21% of patients on
placebo  achieved  at  least  a  one-stage  improvement  in  liver  fibrosis  without  any  worsening  of  NASH  (p  =  0.02)  and  (ii)
approximately  20%  of  OCA-treated  patients  as  compared  to  approximately  7%  of  patients  on  placebo  achieved  NASH
resolution  with  no  worsening  of  fibrosis  (p  =  0.03)  using  the  definition  we  selected  for  NASH  resolution  in  the
REGENERATE trial.

In the FLINT trial, more OCA-treated patients experienced significant improvements in the major histological features
of  NASH,  including  steatosis  (61%  versus  38%,  p  =  0.001),  lobular  inflammation  (53%  versus  35%,  p  =  0.006)  and
hepatocellular ballooning (46% versus 31%, p = 0.03), as compared to the placebo treatment group. Trends were similar
between the two treatment groups for portal inflammation, which is not a component of NAS and is typically mild in adult
NASH patients.

The  histological  improvements  observed  in  OCA-treated  patients  versus  placebo  were  accompanied  by  statistically
significant reductions in relevant biochemical parameters, including the serum liver enzymes ALT (p < 0.0001), aspartate
aminotransferase (“AST”) (p = 0.0001) and gamma-glutamyl transferase (“GGT”) (p < 0.0001), each of which were above
generally accepted normal limits at baseline, and total bilirubin (p = 0.002). A modest but statistically significant increase
in ALP (p < 0.0001) in the OCA treatment group was also observed, but levels remained within typical normal limits.

OCA treatment was associated with serum lipid changes, including increases in total cholesterol and LDL cholesterol
and a decrease in HDL cholesterol, that developed within 12 weeks of treatment initiation, then reversed through the end of
treatment and returned to baseline during the 24-week post-treatment follow-up phase. Based on these observations, lipid
management was emphasized partway into the trial, using accepted guidelines. At 72 weeks as compared to baseline, the
following  effects  were  observed  in  the  OCA  treatment  group:  an  increase  in  mean  total  cholesterol  (0.16  mmol/L  or  6
mg/dL increase OCA versus 0.19 mmol/L or 7mg/dL decrease placebo, p = 0.0009), an increase in mean LDL cholesterol
(0.22 mmol/L or 9 mg/dL increase OCA versus 0.22 mmol/L or 8 mg/dL decrease placebo, p < 0.0001), a decrease in mean
HDL cholesterol (0.02 mmol/L or 1 mg/dL decrease OCA versus 0.03 mmol/L or 1 mg/dL increase placebo, p = 0.01) and
a decrease in triglycerides (0.22 mmol/L or 20 mg/dL decrease OCA versus 0.08 mmol/L or 7 mg/dL decrease placebo, p =
0.88,  not  significant).  These  changes  in  cholesterol  levels,  along  with  the  achievement  of  predefined  efficacy  criteria,
played a role in the decision of the FLINT data and safety monitoring board to terminate the treatment phase of the FLINT
trial, and the publication of the FLINT results noted the need for further study of these changes.

A post-hoc analysis showed OCA-treated patients who initiated statins during the FLINT trial (n = 26) experienced a
rapid  reversal  of  their  observed  mean  LDL  cholesterol  increase  to  below  baseline  levels,  with  a  mean  decrease  after  72
weeks of treatment of -18.9 mg/dL. In contrast, other OCA-treated patients with no reported initiation or change in statin
therapy experienced an increase in LDL cholesterol that peaked at week 12 and was sustained over the 72-week treatment
period.  Patients  treated  with  statins  at  baseline  who  maintained  statin  treatment  over  the  duration  of  the  study  (n  =  50)
experienced a mean LDL cholesterol increase of 8.7 mg/dL at 72 weeks. Patients not treated with statins during the study

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(n = 65) experienced a mean LDL cholesterol increase of 16.0 mg/dL. Treatment related LDL cholesterol increases in all
groups reversed with treatment discontinuation. This analysis suggests that the OCA-associated LDL cholesterol increase
reaches a maximum peak and plateaus soon after initiation of therapy and that concomitant statin use in NASH patients
receiving OCA may mitigate treatment-related LDL cholesterol increases.

In the FLINT trial, statistically significant weight loss of an average of 2.3 kilograms was observed in OCA patients
compared to no weight loss in the placebo group (p = 0.008), and this weight loss reverted towards baseline during the 24-
week follow-up phase. A pre-specified sensitivity analysis conducted by the investigators showed that weight loss was not
a  driver  of  the  primary  endpoint.  An  increase  in  a  marker  of  hepatic  insulin  resistance  known  as  homoeostasis  model
assessment  –  estimated  insulin  resistance  (“HOMA-IR”)  (calculated  using  the  product  of  fasting  plasma  insulin  and
glucose) was observed at 72 weeks in the OCA treatment group (p = 0.01). However, there was an imbalance in baseline
plasma insulin levels (201 pmol/L OCA versus 138 pmol/L placebo), and an even larger relative and absolute increase in
HOMA-IR  was  observed  in  the  placebo  group  at  the  conclusion  of  the  24-week  follow-up  phase.  This  is  potentially
attributable to the inherent variability in HOMA-IR measurements, particularly in patients with type 2 diabetes, that have
been  shown  to  make  single  time-point  to  time-point  changes  of  this  magnitude  clinically  uninterpretable.  There  were
virtually no changes in mean hemoglobin A1c, a measure of average blood sugar control over a period of approximately
three  months,  in  either  OCA  or  placebo  groups  at  72  weeks.  In  an  earlier  study  of  OCA  in  diabetic  NAFLD  patients
employing the hyperinsulinemic-euglycemic insulin clamp, the gold standard for detecting changes in insulin resistance,
OCA improved the glucose disposal rate consistent with reduced insulin resistance.

OCA was generally well tolerated in the FLINT trial. Adverse events were generally mild to moderate in severity and
the  incidence  in  the  OCA  and  placebo  treatment  groups  was  similar  for  all  symptoms  except  pruritus.  Pruritus  occurred
more frequently in the OCA treatment group than in the placebo treatment group (23% vs. 6%, p < 0.0001) and at a higher
grade (predominately moderate pruritus) but resulted in only one patient discontinuation. The incidence of severe or life-
threatening events was not different between the two treatment groups and most of the events in both groups were deemed
to be unrelated to treatment, including all severe or life-threatening cardiovascular events. There were two patient deaths in
the Phase 2b FLINT trial and neither death was considered related to OCA treatment.

OCA and Bezafibrate

In  December  2018,  we  entered  into  the  Aralez  Agreement,  pursuant  to  which  we  acquired  (i)  Aralez’s  license  to
develop  and  commercialize  bezafibrate  in  the  United  States  (as  amended  and  restated  in  connection  therewith,  the
“Bezafibrate License”), (ii) Aralez’s IND on file with the FDA and other associated regulatory documentation and (iii) a
non-exclusive license to certain of Aralez’s intellectual property. Pursuant to the Aralez Agreement, we paid $9.0 million to
Aralez  in  connection  with  the  closing  of  the  transactions  in  December  2018  and  are  obligated  to  make  a  $2.0  million
milestone payment to Aralez based on the occurrence of specified regulatory-related events. Bezafibrate, a PPAR agonist
that  has  been  studied  in  PBC,  is  not  approved  in  the  U.S.  for  any  indication.  We  are  evaluating  the  efficacy,  safety  and
tolerability of bezafibrate in combination with OCA in patients with PBC in a Phase 2 study outside of the United States,
and we filed an IND with the FDA in January 2021 to prepare to expand such development into the United States, with the
longer-term goal of developing and seeking regulatory approval for a fixed dose combination regimen in this indication and
potentially may study this combination in other liver diseases. Pursuant to the Bezafibrate License, we are also obligated to
make a $2.5 million milestone payment based on the occurrence of specified regulatory-related events with respect to such
a  combination  product,  as  well  as  mid-single  digit  percentage  royalty  payments  based  on  the  net  sales  of  such  a
combination product.

Other Product Candidates

The discovery and development of safe and effective new product candidates and the development of additional uses
for our existing product candidates and approved products, are important for the continued strength of our business. We,
together with our collaborators, have discovered several bile acid chemistry-based compounds that are in the early stages of
research  and  development.  Among  these  compounds  is  INT-787.  INT-787  is  an  FXR  agonist  that  we  are  currently
evaluating in preclinical studies. INT-787 has distinct pharmacological properties that differ from those of OCA and has
shown potential anti-fibrotic and anti-inflammatory effects in animal models. We believe that bile acid analogs may have

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utility in a broad range of diseases beyond non-viral liver disease and we have in the past, and may in the future, explore
the potential application of our development compounds outside of our core areas of focus.

The  process  from  discovery  to  development  to  regulatory  approval  of  a  product  candidate  can  take  more  than  ten
years. Product candidates can fail at any stage of the process, and product candidates may not receive regulatory approval
even after many years of research and development and significant investment. In addition, we may decide to terminate or
deprioritize  the  development  of  our  product  candidates  due  to  a  number  of  factors,  including  our  views  of  the  relevant
regulatory  development  pathway,  competitive  landscape,  commercial  viability  of  the  product  candidate,  or  superior
alternative uses of capital. For example, we have studied OCA for PSC, a rare, serious, chronic cholestatic liver disease
characterized  by  a  progressive,  autoimmune-based  destruction  of  bile  ducts  with  eventual  onset  of  cirrhosis.  While  we
believe that the results of our Phase 2 AESOP trial announced in 2017 established a proof of concept of OCA in a second
cholestatic liver disease, we have deprioritized development of OCA in PSC based, in part, on the lack of clarity on the
regulatory pathway for this rare but serious disease. In addition, we are no longer actively developing INT-767, an orally
administered dual FXR and TGR5 agonist derived from the primary human bile acid chenodeoxycholic acid.

Competition

The  biotechnology  and  pharmaceutical  industries  are  intensely  competitive  and  subject  to  rapid  and  significant
technological  change.  We  have  competitors  in  the  United  States,  Europe  and  other  jurisdictions,  including  major
multinational pharmaceutical companies, established biotechnology companies, specialty pharmaceutical and generic drug
companies and universities and other research institutions. Many of our competitors have financial, sales and marketing,
manufacturing  and  distribution,  legal,  regulatory  and  product  development  resources  substantially  greater  than  ours.
Smaller  or  early-stage  companies  may  also  prove  to  be  significant  competitors,  particularly  through  collaborative
arrangements with large, established companies.

The ability of Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, and other future approved products,
if any, to compete with products sold by other companies will depend on a number of factors, including efficacy, safety and
tolerability, reliability, convenience of dosing, price, the level of branded and generic competition and reimbursement. We
believe that the competitive environment for Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH is as
follows.

Ocaliva for PBC

Ocaliva competes with UDCA (or ursodiol), a first-line therapy approved for the treatment of PBC that is available
generically  at  a  significantly  lower  cost  than  Ocaliva.  Additional  product  candidates  in  Phase  3  or  earlier  clinical  or
preclinical  development  for  the  treatment  of  PBC  include  Genfit  SA’s  dual  PPAR  alpha/delta  agonist  (elafibranor),
CymaBay’s  PPAR  delta  agonist  (seladelpar),  Genkyotex’s  NOX1/NOX4  inhibitor  (setanaxib),  HighTide’s  AMPK
activator/FXR agonist combination (HTD1801) and Fast Forward Pharmaceuticals BV’s anti-CD40 monoclonal antibody
(FFP104).  Additionally,  several  companies  have  product  candidates  aimed  at  the  cholestatic-induced  pruritus  associated
with  PBC,  including  apical  sodium  dependent  bile  acid  transport  inhibitors  being  developed  by  GlaxoSmithKline  plc
(GSK2330672).

Off-label uses of other potential treatments may also compete with Ocaliva for PBC. For example, while fibrates are
not approved for use in PBC, off-label use of fibrate drugs has been reported. Bezafibrate, a fibrate that is not approved by
the FDA for any indication and is only available outside of the United States, has been studied in PBC.

OCA for Liver Fibrosis Due to NASH

There are currently no medications approved for the treatment of NASH. However, various therapeutics are used off-
label for the treatment of NASH, including vitamin E (an antioxidant), insulin sensitizers (e.g., metformin, pioglitazone),
antihyperlipidemic agents (e.g., gemfibrozil), pentoxifylline and UDCA. There are several product candidates in Phase 3 or
earlier  clinical  or  preclinical  development  for  the  treatment  of  NASH,  including  Madrigal’s  THR  beta  agonist
(resmetirom), Novo Nordisk’s GLP1 agonist (semaglutide), and Inventiva’s pan-PPAR agonist (lanifibranor), as well as

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FXR agonists from Novartis AG (tropifexor, nidufexor), Metacrine (MET409, MET642), Terns Pharmaceuticals (TERN-
101), Gilead Sciences, Inc. (cilofexor) and Enanta Pharmaceuticals, Inc. (EDP-305).

Additional pharmaceutical and biotechnology companies with product candidates in development for the treatment of
NASH include AstraZeneca plc, Altimmune Inc., Boehringer Ingelheim GmbH, Bristol-Myers Squibb Company, Durect
Corporation,  Galectin  Therapeutics  Inc.,  Galmed  Pharmaceuticals  Ltd.,  Immuron  Ltd.,  Ionis  Pharmaceuticals,  Inc.,  Islet
Sciences,  Inc.,  Madrigal  Pharmaceuticals,  Inc.,  MediciNova,  Inc.,  MiNA  Therapeutics,  NGM  Biopharmaceuticals,  Inc.,
NuSirt  Sciences  Inc.,  Pfizer  Inc.,  Viking  Therapeutics,  Inc.  and  Zydus  Pharmaceuticals  (USA)  Inc.  NASH  is  a  complex
disease and we believe that it is unlikely that any one therapeutic option will be optimal for every NASH patient.

In  addition,  many  universities  and  private  and  public  research  institutions  may  become  active  in  our  target  disease
areas. The results from our clinical trials and the approval of Ocaliva for PBC have brought more attention to our targeted
indications  and  bile  acid  chemistry.  As  a  result,  we  believe  that  additional  companies  and  organizations  may  seek  to
compete with us in the future. Our competitors may succeed in developing, acquiring or licensing on an exclusive basis,
technologies and drug products that are more effective or less costly than OCA or any other product candidates that we are
currently  developing  or  that  we  may  develop,  which  could  render  our  products  or  product  candidates  obsolete  and
noncompetitive. Our ability to compete may also be affected because, in many cases, insurers or other third-party payors
seek to encourage the use of generic products.

Intellectual Property

Protecting our intellectual property, such as our patents, is a key part of our strategy. We are the owner of record of
numerous  issued  U.S.  and  non-U.S.  patents  with  claims  directed  to  pharmaceutical  compounds,  pharmaceutical
compositions,  methods  of  making  these  compounds  and  methods  of  using  these  compounds  in  various  indications.  In
addition,  we  are  the  owner  of  record  of  numerous  pending  U.S.  and  non-U.S.  patent  applications,  and  regularly  pursue
additional patent applications in various jurisdictions. We also have numerous trademark and service mark registrations and
pending trademark and service mark applications in the United States and abroad.

The patent portfolio for OCA contains U.S. and non-U.S. patents and patent applications directed to compositions of
matter, methods of use and manufacturing methods. Our primary composition of matter patent for OCA was to expire in
2022. In light of the U.S. marketing approval of Ocaliva for PBC in May 2016, we applied for an extension of the patent
term for this patent in the United States into 2027, which extension has been granted. In addition, in connection with the
conditional approval of Ocaliva for PBC in the European Union, we have applied for supplementary patent certification
(“SPC”) to extend the patent term for this patent in the European Union into 2027. To date, we have received grants of SPC
in Austria, Cyprus, Denmark, Finland, France, Germany, Greece, Ireland, Italy, Norway, Portugal, Spain and Sweden and
we expect to take similar actions in other jurisdictions and countries where similar regulations exist.

The table set forth below summarizes the U.S. patents covering OCA that are listed in the FDA’s Orange Book List of
Approved  Drug  Products  With  Therapeutic  Equivalence  Evaluations  (the  “Orange  Book”).  The  issued  patents  covering
OCA are expected to expire in 2022 at the earliest and 2036 at the latest if the appropriate maintenance, renewal, annuity,
or  other  government  fees  are  paid.  We  expect  that  the  patents  in  the  OCA  portfolio  that  are  listed  in  the  Orange  Book
would expire as set forth below, assuming the appropriate maintenance, renewal, annuity or other governmental fees are
paid.

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Patent No.
RE 48,286

8,058,267
8,377,916
9,238,673

Type of Patent(1)
  Composition of 

Matter

  Claims OCA compound

Brief Summary of Patent

  Method of Use
  Method of Use
  Composition of 

  Claims methods of treating PBC with OCA
  Claims methods of treating PBC with OCA
  Claims OCA active pharmaceutical ingredient 

Matter

(“API”)

10,047,117

  Method of Use

  Claims methods of treating FXR mediated

diseases 
with OCA API

10,052,337

  Composition of 

  Claims OCA finished drug product

Matter

10,174,073

  Composition of

  Claims OCA API produced by a specified process  

10,751,349

10,758,549

Matter
Composition of
Matter
Method of Use

Claims OCA finished drug product

Claims methods of treating PBC with OCA

U.S. Patent
Expiration
2027

2022
2022
2033

2033

2036

2033

2036

2036

(1) You should read the risk factors included elsewhere in this Annual Report on Form 10-K for important information
about  risks  posed  by  the  loss  of  patent  protection,  in  particular  the  risks  described  under  “Risk  Factors  —  Risks
Related to Our Intellectual Property.”

In addition, we have intellectual property protecting OCA that we would expect to list in the Orange Book if OCA is

approved for the treatment of NASH.

We  may  rely  on  trade  secrets  to  protect  our  proprietary  technologies,  especially  where  we  do  not  believe  patent
protection  is  appropriate  or  obtainable.  However,  trade  secrets  are  difficult  to  protect.  We  rely  in  part  on  confidentiality
agreements with our employees, consultants, outside scientific collaborators, sponsored researchers and other advisors to
protect our trade secrets and other proprietary information. We also seek to preserve the integrity and confidentiality of our
data, trade secrets and know-how by maintaining physical security of our premises and physical and electronic security of
our information technology systems.

Our commercial success will depend in part on our ability to obtain and maintain patent, trademark and trade secret
protection covering our products such as Ocaliva and product candidates, as well as our ability to successfully defend our
intellectual property against third-party challenges. Our ability to stop third parties from making, using, selling, offering to
sell  or  importing  our  products  is  dependent  upon  the  extent  to  which  we  have  regulatory  exclusivity  or  intellectual
property-based exclusivity rights under valid and enforceable patents or other intellectual property that cover our products.
If we fail to obtain and maintain adequate intellectual property protection, we may not be able to prevent third parties from
launching generic versions of our products, from using our proprietary technologies or from marketing products that are
very  similar  or  identical  to  ours.  The  patent  positions  of  pharmaceutical  companies  can  be  highly  uncertain  and  involve
complex legal and factual questions for which important legal principles remain unresolved. No consistent policy regarding
the breadth of claims allowed in pharmaceutical patents has emerged to date in the United States or in foreign jurisdictions,
and the legal standards relating to the patentability, validity and enforceability of pharmaceutical patents are evolving.

Changes in either the patent laws or in interpretations of patent laws in U.S. and foreign jurisdictions may diminish the
value of our intellectual property. Accordingly, we cannot predict the breadth of claims that may be enforced in the patents
that we currently own or that may issue from the applications we have filed or may file in the future or those that we may
license from third parties. Additionally, our currently pending or future patent applications may not result in issued patents,
and any term extensions that we seek may not be granted. Further, if any patents we obtain or license are deemed invalid or
unenforceable, it could impact our ability to commercialize or license our technology or enable third parties to develop and
market products that are similar or identical to ours.

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Manufacturing and Supply

We  do  not  own  or  operate  manufacturing  facilities  for  the  production  of  Ocaliva,  OCA  or  any  of  our  other  product
candidates, and we do not have any plans to develop our own manufacturing operations in the foreseeable future. We rely
on third-party contract manufacturers for all of our required raw materials, API and finished product for our commercial
sales and for our clinical trials and preclinical studies.

We  source  the  manufacture  and  commercial  supply  of  API  from  such  manufacturers,  for  use  in  Ocaliva  and,  if
approved, OCA for liver fibrosis due to NASH. We believe that we have secured supplies of API sufficient to meet our
PBC  and  NASH  commercial  supply  requirements  during  the  initial  stages  of  our  NASH  launch  following  the  expected
approval of OCA for liver fibrosis due to NASH. One such supply agreement is with PharmaZell GmbH (“PharmaZell”).
That contract does not require us to purchase a specific percentage of our annual commercial requirements of API from
PharmaZell. We have also qualified an additional API supplier from which we may currently acquire API on a purchase
order basis and continue to engage in activities intended to ensure that our long-term commercial supply requirements are
satisfied.  In  connection  with  such  efforts,  we  entered  into  an  agreement  with  a  third  potential  supplier  of  API  for  the
manufacture  of  Ocaliva  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH,  under  which  we  may  in  the  future  be
obligated to purchase a portion of our API requirements in the event of the achievement of agreed regulatory and product
development milestones.

We do not have long-term supply agreements for any of our product candidates other than OCA, and regularly obtain
supplies and services relating to our product candidates from third-party contract manufacturers on a purchase order basis.
Contract manufacturers are subject to extensive governmental regulation and we depend on them for compliance with the
requirements of U.S. and non-U.S. regulators for the manufacture of our finished products, including Ocaliva. We intend to
continue  to  rely  on  third-party  manufacturers  for  the  manufacture  of  clinical  supplies  of  our  product  candidates  and
commercial supplies of our approved products, including Ocaliva and, if approved, OCA for liver fibrosis due to NASH.
We  believe  this  manufacturing  strategy  will  enable  us  to  direct  financial  resources  to  the  development  and
commercialization of products rather than diverting resources to establishing a manufacturing infrastructure. If  PharmaZell
and our other current and future suppliers are not able to meet our on-going commercial supply requirements, including
those relating to Ocaliva or, if approved, OCA for liver fibrosis due to NASH, on acceptable terms, or at all, our business
may  be  materially  and  adversely  affected.  See  “Risk  Factors  —  Risks  Related  to  the  Development  and  the  Regulatory
Review and Approval of Our Products and Product Candidates — We rely entirely on third parties for the manufacture of
our product requirements for our preclinical studies and clinical trials, as well as our commercial supply of Ocaliva and, if
approved, OCA for liver fibrosis due to NASH and our other product candidates, and also depend on third-party vendors
and CROs for certain of our clinical trial and product development activities. Our business could be harmed if our third-
party manufacturers fail to provide us with sufficient quantities of drug product, or fail to do so at acceptable quality levels
or prices, or if our third-party vendors or CROs assisting us with our clinical trials and product development activities fail
to comply with their contractual commitments or applicable regulatory obligations or if we lose our relationships with our
third-party vendors and CROs.”

Sales and Marketing

Ocaliva is our first approved product and the commercial launch of Ocaliva for PBC is our first product launch. We are
commercializing  Ocaliva  for  PBC  using  a  combination  of  our  internal  commercial  organization,  a  contract  sales
organization and third-party distributors depending on the jurisdiction. We are developing our commercialization strategy
for OCA for liver fibrosis due to NASH, if approved, and have not yet decided on our commercialization strategy for OCA
for other indications or for our other product candidates, in each case, if approved. We intend to continue to evaluate how
best  to  commercialize  our  product  candidates,  if  approved,  in  the  United  States  and  internationally,  and  may  choose  to
collaborate  with  third  parties  that  have  sales  and  marketing  capabilities  and  established  distribution  systems,  either  to
augment our own capabilities or in lieu thereof.

Customers

We  commenced  our  commercial  launch  of  Ocaliva  for  the  treatment  of  PBC  in  the  United  States  in  June  2016.  In

December 2016, the European Commission granted conditional approval for Ocaliva for the treatment of PBC and we

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commenced our European commercial launch in January 2017. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia. We
recognized net product sales of Ocaliva of $312.7 million, $249.6 million and $177.8 million for the years ended December
31, 2020, 2019 and 2018, respectively. We sell Ocaliva to a limited number of specialty pharmacies which dispense the
product directly to patients. The specialty pharmacies are referred to as our customers. For a discussion of our customer
concentration,  see  Note  2  to  our  audited  consolidated  financial  statements  included  elsewhere  in  this  Annual  Report  on
Form 10-K.

Government Regulation and Product Approval

Government  authorities  in  the  United  States,  at  the  federal,  state  and  local  level,  and  analogous  authorities  in  other
countries  extensively  regulate,  among  other  things,  the  research,  development,  testing,  manufacture,  recordkeeping,
approval, labeling, packaging, promotion, storage, advertising, distribution, marketing, sampling, post-approval monitoring
and reporting and export and import of products such as Ocaliva and those we are developing. Our product candidates must
be approved by the FDA through the NDA process before they may be legally marketed in the United States and by the
European  Commission  following  a  favorable  assessment  provided  by  the  EMA  through  the  MAA  process  for  a  product
falling  within  the  scope  of  the  Centralized  procedure  or  a  national  MAA  process  (albeit  through  the  process  of  Mutual
Recognition  or  Decentralized  procedure)  before  they  may  be  legally  marketed  in  the  European  Union.  Our  product
candidates will be subject to similar requirements in other countries prior to marketing in those countries. The process of
obtaining regulatory approvals and the subsequent compliance with applicable federal, state, local and foreign statutes and
regulations require the expenditure of substantial time and financial resources.

United States Government Regulation

NDA Approval Processes

In  the  United  States,  the  FDA  regulates  drugs  under  the  Federal  Food,  Drug,  and  Cosmetic  Act,  as  amended  (the
“FDCA”) and implementing regulations. An applicant seeking approval to market and distribute a new drug product in the
United States must typically undertake the following:

● completion of preclinical laboratory tests, animal studies and formulation studies in compliance with the FDA’s

good laboratory practice regulations;

● submission to the FDA of an IND, which must take effect before human clinical testing may begin;

● approval by an independent institutional review board (“IRB”), representing each clinical site before each clinical

trial may be initiated;

● performance  of  adequate  and  well-controlled  human  clinical  trials  in  accordance  with  good  clinical  practices
(“GCP”) to establish the safety and efficacy of the new drug product for each indication for which FDA approval
is sought;

● preparation and submission to the FDA of a NDA;

● review of the new drug product by an FDA advisory committee, where appropriate or if applicable, although the

FDA is not bound by the recommendation of an advisory committee;

● satisfactory completion of one or more FDA inspections of the manufacturing facility or facilities at which the
new drug product, or components thereof, are produced to assess compliance with current Good Manufacturing
Practices (“cGMP”) requirements and to assure that the facilities, methods and controls are adequate to preserve
the new drug product’s identity, strength, quality and purity;

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● satisfactory completion of FDA audits of clinical trial sites to assure compliance with GCP and the integrity of

the clinical data;

● payment of user fees and procurement of FDA approval of the NDA; and

● compliance  with  any  post-approval  requirements,  including,  as  applicable,  Risk  Evaluation  and  Mitigation

Strategies (“REMS”) and post-approval studies required by the FDA.

Preclinical and Clinical Studies

Once  a  pharmaceutical  candidate  is  identified  for  development,  it  enters  the  preclinical  or  nonclinical  testing  stage.
Nonclinical tests include laboratory evaluations of product chemistry, toxicity and formulation, as well as animal studies.
An IND sponsor must submit the results of the nonclinical tests, together with manufacturing information and analytical
data, to the FDA as part of the IND. Some nonclinical testing may continue even after the IND is submitted. In order to
conduct  clinical  research,  an  IND  sponsor  must  submit  an  IND.  An  IND  automatically  becomes  effective  30  days  after
receipt by the FDA, unless the FDA, within the 30-day time period, or any time thereafter, places the IND on clinical hold.
In  such  a  case,  the  IND  sponsor  and  the  FDA  must  resolve  any  outstanding  concerns  before  clinical  trials  can  begin  or
continue. A clinical hold may affect one or more specific studies or all studies conducted under the IND.

All clinical trials must be conducted under the supervision of one or more qualified investigators in accordance with
GCPs.  They  must  be  conducted  under  protocols  detailing  the  objectives  of  the  trial,  dosing  procedures,  research  subject
selection and exclusion criteria and the safety and effectiveness criteria to be evaluated. Each protocol must be submitted to
the FDA as part of the IND, and progress reports detailing the status of the clinical trials must be submitted to the FDA
annually. Sponsors also must timely report to the FDA serious and unexpected adverse reactions, any clinically important
increase in the rate of a serious suspected adverse reaction over that listed in the protocol or investigation brochure, or any
findings from other studies or animal or in vitro testing that suggest a significant risk in humans exposed to the drug. An
IRB at each institution must, among other things, review and approve the protocol before a clinical trial commences at such
institution,  and  approve  the  consent  form  that  must  be  provided  to  each  research  subject  or  the  subject’s  legal
representative, monitor the study until completed and otherwise comply with regulations applicable to the IRB.

Human  clinical  trials  are  typically  conducted  in  three  sequential  phases,  although  the  phases  may  overlap  or  be

combined:

● Phase  1.  The  drug  is  initially  introduced  into  healthy  human  subjects  and  tested  to  assess  pharmacological
actions, safety, dosage tolerance, absorption, metabolism, distribution and elimination and, in some cases, early
evidence  of  effectiveness.  In  the  case  of  some  products  intended  for  the  treatment  of  severe  or  life-threatening
diseases,  such  as  cancer,  especially  when  the  product  may  be  inherently  too  toxic  to  ethically  administer  to
healthy volunteers, the initial human testing is often conducted in patients.

● Phase 2. Clinical trials are performed on a limited patient population intended to identify possible adverse effects
and  safety  risks,  to  preliminarily  evaluate  the  efficacy  of  the  product  for  specific  targeted  diseases  and  to
determine dosage tolerance and optimal dosage.

● Phase 3.  Clinical  trials  are  undertaken  to  further  evaluate  dosage,  clinical  efficacy  and  safety  in  an  expanded
patient  population  generally  at  geographically  dispersed  clinical  study  sites.  These  studies  are  intended  to
establish the overall risk-benefit ratio of the product and provide an adequate basis for product labeling, should it
ultimately be approved for marketing. In most cases the FDA requires two adequate and well-controlled Phase 3
clinical trials with statistically significant results to demonstrate the efficacy of the drug. A single Phase 3 clinical
trial with other confirmatory evidence may be sufficient in certain instances.

Human  clinical  trials  are  inherently  uncertain  and  Phase  1,  Phase  2  and  Phase  3  testing  may  not  be  successfully
completed. The FDA or the sponsor may suspend a clinical trial at any time for a variety of reasons, including a finding
that the research subjects or patients are being exposed to an unacceptable health risk. Similarly, an IRB can suspend or

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terminate approval of a clinical trial at its institution if the clinical trial is not being conducted in accordance with the IRB’s
requirements or if the drug has been associated with unexpected serious harm to patients. In some cases, clinical trials are
overseen by an independent group of qualified experts organized by the trial sponsor, or the clinical monitoring board or
data monitoring committee. This group typically provides recommendations to the trial sponsor for whether or not a trial
may move forward at designated check points. These decisions are based on the data monitoring committee’s independent
review of data from the ongoing trial.

Sponsors of clinical trials of certain FDA-regulated products, including prescription drugs, are required to register and
disclose clinical trial information related to the product, patient population, phase of investigation, clinical trial sites and
investigator, and other aspects of the clinical trial on a public website maintained by the U.S. National Institutes of Health.
Sponsors  are  also  obligated  to  disclose  the  results  of  these  clinical  trials  after  completion.  For  a  new  product  or  a  new
indication for a previously approved product, sponsors can delay submission of clinical study results for up to two years
until the product has been approved or approved for the new use. Competitors and others may use this publicly-available
information to gain knowledge regarding the design and progress of our development programs.

During  the  development  of  a  new  drug,  sponsors  are  given  opportunities  to  meet  with  the  FDA  at  certain  points,
including prior to the submission of an IND, at the end of Phase 2 and before a NDA is submitted. Meetings at other times
may be requested. These meetings can provide an opportunity for the sponsor to share information about the data gathered
to  date  and  for  the  FDA  to  provide  advice  and  feedback  on  the  next  phase  of  development.  Sponsors  typically  use  the
meeting at the end of Phase 2 to discuss their Phase 2 clinical results and present their plans for the pivotal Phase 3 clinical
trial(s) that they believe will support the approval of the new drug. If a Phase 2 clinical trial is the subject of discussion at
the end of Phase 2 meeting with the FDA, a sponsor may be able to request a special protocol assessment (“SPA”), the
purpose of which is to reach agreement with the FDA on the Phase 3 clinical trial protocol design and analysis that will
form the primary basis of an efficacy claim.

According to published guidance on the SPA process, a sponsor which meets the prerequisites may make a specific
request  for  an  SPA  and  provide  information  regarding  the  design  and  size  of  the  proposed  clinical  trial.  The  FDA  is
supposed to evaluate the protocol within 45 days of the request to assess whether the proposed trial is adequate, and that
evaluation  may  result  in  discussions  and  a  request  for  additional  information.  An  SPA  request  must  be  made  before  the
proposed trial begins, and all open issues must be resolved before the trial begins. If a written agreement is reached, it will
be documented and made part of the record. The agreement is generally expected to be binding on the FDA, in that the
critical design elements agreed to as part of an SPA agreement may not be changed by the sponsor or the FDA after the
trial  begins  except  with  the  written  agreement  of  the  sponsor  and  the  FDA  or  if  the  FDA  determines  that  a  substantial
scientific  issue  essential  to  determining  the  safety  or  efficacy  of  the  drug  was  identified  after  the  testing  began.  The
presence of an SPA agreement does not guarantee that a marketing application will be filed or approved, even if the trial is
conducted  in  accordance  with  the  protocol  and  achieves  the  specified  endpoints.  In  rare  cases,  the  FDA  may  rescind  an
SPA agreement.

Concurrent with clinical trials, sponsors usually complete additional animal safety studies and also develop additional
information  about  the  chemistry  and  physical  characteristics  of  the  drug  and  finalize  a  process  for  manufacturing
commercial quantities of the product in accordance with cGMP requirements. The manufacturing process must be capable
of consistently producing quality batches of the drug and the manufacturer must develop methods for testing the quality,
purity  and  potency  of  the  drug  prior  to  release.  Additionally,  appropriate  packaging  must  be  selected  and  tested  and
stability  studies  must  be  conducted  to  demonstrate  that  the  drug  candidate  does  not  undergo  unacceptable  deterioration
over its proposed shelf-life.

The  results  of  product  development,  nonclinical  studies  and  clinical  trials,  along  with  descriptions  of  the
manufacturing process, analytical tests and other control mechanisms, proposed labeling and other relevant information are
submitted to the FDA as part of a NDA requesting approval to market the product. The submission of a NDA is subject to
the  payment  of  user  fees,  but  a  waiver  of  such  fees  may  be  obtained  under  specified  circumstances.  Currently,  the
application  fee  is  approximately  $2.9  million  for  NDAs  with  clinical  data  and  approximately  $1.5  million  for  NDAs
without  clinical  data.  The  sponsor  under  an  approved  NDA  is  also  subject  to  annual  program  user  fees,  currently
approximately $336,000. Program fees are assessed for each approved prescription drug product identified in an approved
application, up to five program fees per application. These fees are typically modified annually. The FDA reviews all

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NDAs submitted to ensure that they are sufficiently complete for substantive review before it accepts them for filing. It
may request additional information rather than accept a NDA for filing. In this event, the NDA must be resubmitted with
the additional information. The resubmitted application also is subject to review before the FDA accepts it for filing.

Once  the  NDA  is  accepted  for  filing,  the  FDA  begins  an  in-depth  review.  NDAs  receive  either  standard  or,  as
discussed more fully below, priority review. The FDA may refuse to approve a NDA if the applicable regulatory criteria are
not  satisfied  or  may  require  additional  clinical  or  other  data.  Even  if  such  data  are  submitted,  the  FDA  may  ultimately
decide that the NDA does not satisfy the criteria for approval. The FDA reviews a NDA to determine, among other things,
whether a product is safe, effective, and can be properly manufactured for its intended use or uses. The FDA may refer the
NDA  to  an  advisory  committee  for  review  and  recommendation  as  to  whether  the  application  should  be  approved  and
under what conditions. The FDA is not bound by the recommendation of an advisory committee. Before approving a NDA,
the  FDA  will  inspect  the  facility  or  facilities  where  the  product  is  manufactured  and  tested  to  ensure  compliance  with
cGMPs.  An  approval  letter  from  the  FDA  authorizes  commercial  marketing  of  the  product  and  specifies  the  prescribing
information for the approved indication(s).

Fast Track, Breakthrough Therapy, Priority Review and Accelerated Approval

The  FDA  is  authorized  to  designate  certain  products  for  expedited  review  if  they  are  intended  to  address  an  unmet
medical  need  in  the  treatment  of  a  serious  or  life-threatening  disease  or  condition.  These  programs  include  fast  track
designation, breakthrough therapy designation and priority review designation.

Specifically, the FDA may designate a product for fast track review if it is intended, whether alone or in combination
with one or more other drugs, for the treatment of a serious or life-threatening disease or condition, and it demonstrates the
potential to address unmet medical needs for such a disease or condition. For fast track designated products, sponsors may
have a higher number of interactions with the FDA and the FDA may initiate review of sections of a fast track product’s
NDA before the application is complete.

A product may also be designated as a breakthrough therapy if it is intended, either alone or in combination with one
or more other drugs, to treat a serious or life-threatening disease or condition and preliminary clinical evidence indicates
that  the  product  may  demonstrate  substantial  improvement  over  existing  therapies  on  one  or  more  clinically  significant
endpoints, such as substantial treatment effects observed early in clinical development. The FDA may take certain actions
with respect to breakthrough therapies, including holding meetings with the sponsor throughout the development process;
providing  timely  advice  to  the  product  sponsor  regarding  development  and  approval;  involving  more  senior  staff  in  the
review process; assigning a cross-disciplinary project lead for the review team; and taking other steps to design the clinical
trials in an efficient manner.

The FDA may also designate a product for priority review if it would provide a significant improvement in the safety
or effectiveness of the treatment, diagnosis or prevention of a serious condition. Certain other applications may also qualify
for  priority  review.  The  FDA  determines,  on  a  case-by-case  basis,  whether  the  proposed  drug  represents  a  significant
improvement when compared with other available therapies. A priority designation by the FDA is intended to direct the
agency’s attention and resources to the evaluation of such applications, and to shorten the FDA’s goal for taking action on a
marketing application from ten months to six months.

In addition, the FDA may grant accelerated approval to a drug for a serious or life-threatening condition that provides
meaningful  therapeutic  advantage  to  patients  over  existing  treatments  based  upon  a  determination  that  the  drug  has  an
effect  on  a  surrogate  endpoint  that  is  reasonably  likely  to  predict  clinical  benefit.  The  FDA  may  also  grant  accelerated
approval  for  such  a  condition  when  the  product  has  an  effect  on  an  intermediate  clinical  endpoint  that  can  be  measured
earlier than an effect on irreversible morbidity or mortality, and that is reasonably likely to predict an effect on irreversible
morbidity or mortality or other clinical benefit, taking into account the severity, rarity, or prevalence of the condition and
the  availability  or  lack  of  alternative  treatments.  Drugs  granted  accelerated  approval  must  meet  the  same  statutory
standards  for  safety  and  effectiveness  as  those  granted  traditional  approval.  In  the  case  of  unprecedented  accelerated
approval endpoints, this determination occurs during the review of the NDA. Unless otherwise informed by the FDA, an
applicant  must  submit  to  the  FDA  for  consideration  during  the  preapproval  review  period  copies  of  all  promotional
materials, including promotional labeling as well as advertisements, intended for dissemination or publication within 120

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days following marketing approval. After 120 days following marketing approval, unless otherwise informed by the FDA,
the applicant must submit promotional materials at least 30 days prior to the intended time of initial dissemination of the
labeling or initial publication of the advertisement.

As  a  condition  of  a  grant  of  accelerated  approval,  the  FDA  may  require  that  the  sponsor  perform  one  or  more
controlled post-marketing clinical trials. Approval of a drug may be withdrawn if these trials fail to verify clinical benefit
or  do  not  demonstrate  sufficient  clinical  benefit  to  justify  the  risks  associated  with  the  drug  (e.g.,  show  a  significantly
smaller magnitude or duration of benefit than was anticipated based on the observed effect on the surrogate).

Ocaliva was granted fast track designation by the FDA for the treatment of patients with PBC who have an inadequate
response to or are intolerant of UDCA. In August 2015, the FDA accepted for review our NDA and granted priority review
for Ocaliva in PBC. On May 27, 2016, Ocaliva was approved under the accelerated approval pathway in the United States
for PBC in combination with UDCA in adults with an inadequate response to UDCA, or as monotherapy in adults unable
to tolerate UDCA.

In January 2015, OCA for liver fibrosis due to NASH was granted breakthrough therapy designation by the FDA for
the treatment of patients with NASH with liver fibrosis. In November 2019, the FDA accepted for review our NDA and
granted  priority  review  for  OCA  for  liver  fibrosis  due  to  NASH.  In  June  2020,  we  received  a  complete  response  letter
(“CRL”)  from  the  FDA  stating  that  our  NDA  for  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH  could  not  be
approved in its present form. The CRL indicated that, based on the data the FDA had reviewed, the FDA has determined
that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
At  that  time,  the  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the
ongoing REGENERATE trial in support of potential accelerated approval and that the long-term outcomes phase of the
trial should continue. We are in discussions with the FDA with respect to the potential resubmission of our NDA seeking
accelerated approval of OCA for the treatment of liver fibrosis due to NASH. We had our end of review meeting with the
FDA in October 2020 to discuss the FDA’s risk-benefit assessment in the CRL based on its review of the available data, as
well  as  our  proposed  resubmission  of  our  NDA  for  the  treatment  of  liver  fibrosis  due  to  NASH.  The  meeting  was
constructive  and  the  FDA  has  provided  us  with  helpful  guidance  regarding  supplemental  data  we  can  provide  to  further
characterize OCA’s efficacy and safety profile that could support resubmission based on our Phase 3 REGENERATE 18-
month biopsy data, together with a safety update from our ongoing studies. We are advancing accordingly and plan to hold
additional meetings with the FDA with the goal of achieving sufficient alignment to proceed on this basis and potentially
resubmit our NDA for the treatment of liver fibrosis due to NASH by the end of 2021.

Post-approval Requirements

Drugs manufactured or distributed pursuant to FDA approvals are subject to pervasive and continuing regulation by
the FDA post-approval, including, among other things, requirements relating to recordkeeping, periodic reporting, product
sampling  and  distribution,  advertising  and  promotion  and  reporting  of  adverse  experiences  with  the  product.  Once  an
approval is granted, the FDA may withdraw the approval if compliance with regulatory requirements is not maintained or
if safety or other problems occur after the product reaches the market. Later discovery of previously unknown problems
with a product may result in new labeling information (e.g., warnings), customer training and/or education requirements,
restrictions  on  the  product  or  even  complete  withdrawal  of  the  product  from  the  market.  After  approval,  some  types  of
changes to the approved product, such as adding new indications, manufacturing changes and additional labeling claims,
are subject to further FDA review and approval. In addition, the FDA may require studies, trials, analyses, and surveillance
programs  to  monitor  or  evaluate  the  effect  of  approved  products  that  have  been  commercialized,  and  the  FDA  has  the
power to limit further marketing of a product, or seek withdrawal of approval, based on the results of these post-marketing
programs.

Drug manufacturers and other entities involved in the manufacture and distribution of approved drugs are required to
register their establishments with the FDA and certain state agencies, and are subject to periodic unannounced inspections
by the FDA and some state agencies for compliance with cGMP and other laws. Changes to the manufacturing process are
strictly  regulated  and  often  require  prior  FDA  approval  before  being  implemented.  FDA  regulations  also  require
investigation and correction of any deviations from cGMP and impose reporting and documentation requirements upon

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the  sponsor  and  any  third-party  manufacturers  that  the  sponsor  may  decide  to  use.  Accordingly,  manufacturers  must
continue to expend time, money, and effort in the area of production and quality control to maintain cGMP compliance.

Failure  to  comply  with  the  applicable  U.S.  requirements  at  any  time  during  the  product  development  process  or
approval process, or after approval, may subject us to judicial, regulatory or statutory sanctions, any of which could have a
material adverse effect on us.

These sanctions could include:

● refusal to approve pending applications;

● withdrawal of an approval;

● imposition of a clinical hold;

● warning or untitled letters;

● product recalls;

● product seizures;

● total or partial suspension of production or distribution; and

● injunctions, fines, disgorgement, civil penalties and criminal prosecution.

The  FDA  and  other  U.S.  state  and  federal  authorities  regulate  marketing,  labeling,  advertising  and  promotion  of
products  that  are  placed  on  the  market.  Drugs  may  be  promoted  only  for  the  approved  indications  and  in  a  manner
otherwise  consistent  with  the  provisions  of  the  approved  label  and  FDA  regulations.  The  FDA  and  other  authorities
actively  enforce  the  laws  and  regulations  prohibiting  false,  misleading,  deceptive,  or  off-label  promotional  practices;
violations of these prohibitions can lead to significant liability. Additional regulations apply for advertising and promotion
of  products  approved  under  the  accelerated  approval  pathway.  For  example,  unless  otherwise  informed  by  the  FDA,  an
applicant  must  submit  to  the  FDA  for  consideration  during  the  preapproval  review  period  copies  of  all  promotional
materials, including promotional labeling as well as advertisements, intended for dissemination or publication within 120
days following marketing approval. After 120 days following marketing approval, unless otherwise informed by the FDA,
the applicant must submit promotional materials at least 30 days prior to the intended time of initial dissemination of the
labeling or initial publication of the advertisement.

We rely, and expect to continue to rely, on third parties for the production of clinical and commercial quantities of our
products. Future FDA and state inspections may identify compliance issues at the facilities of our contract manufacturers
that may disrupt production or distribution, or require substantial resources to correct.

From  time  to  time,  legislation  is  introduced  and  passed  in  Congress  that  could  significantly  change  the  statutory
provisions  governing  the  approval,  manufacturing  and  marketing  of  products  regulated  by  the  FDA.  In  addition,  FDA
regulations and guidance are often revised or reinterpreted by the agency in ways that may significantly affect our business
and our products. It is impossible to predict whether legislative changes will be enacted, or FDA regulations, guidance or
interpretations changed or what the impact of such changes, if any, may be.

In  accordance  with  the  applicable  requirements  under  the  accelerated  approval  pathway,  we  initiated  our  Phase  4
COBALT clinical outcomes confirmatory trial for Ocaliva in PBC in December 2014, following discussions with the FDA.
The study evaluates subjects across the spectrum of PBC disease, including early and advanced PBC. We have also agreed
to evaluate the safety and efficacy of Ocaliva in patients with moderate to severe hepatic impairment in a study known as
the 401 trial and as monotherapy in patients with PBC. In addition, we have agreed to develop and characterize a lower
dose formulation of Ocaliva to allow for once daily dosing in patients with moderate or advanced hepatic impairment. We

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are  in  discussions  with  the  FDA  and  the  EMA  with  respect  to  the  status  of  the  COBALT  trial  and  the  401  trial  and
proposals for modifications to these post-marketing studies.

Risk Evaluation and Mitigation Strategy

The Food and Drug Administration Amendments Act of 2007 created a new section of the FDCA which authorizes the
FDA to require a REMS as a condition of NDA approval, or based upon new safety information regarding an approved
drug, when the FDA determines a REMS is necessary to ensure that the benefits of a drug outweigh the potential risks.
Under  a  REMS,  the  FDA  may  require  various  measures  to  address  serious  risks,  such  as  medication  guides,
communication plans, training or registries, as well as steps to monitor and assess the effectiveness of those measures. Such
requirements may impose significant burdens on prescribers, pharmacists or patients. The requirement for a REMS may
materially affect the potential market and profitability of a drug.

We do not have a REMS for Ocaliva for the treatment of PBC.

Patent Term Extension and Data Exclusivity

Depending upon the timing, duration and specifics of FDA approval of the use of our drug candidates, some of our
U.S.  patents  may  be  eligible  for  limited  patent  term  extension  under  the  Drug  Price  Competition  and  Patent  Term
Restoration Act of 1984, (the “Hatch-Waxman Act”). The Hatch-Waxman Act permits an extension of a patent term of up
to  five  years  as  compensation  for  patent  term  lost  during  product  development  and  the  FDA  regulatory  review  process.
However, the extension of patent term cannot extend the remaining term of a patent beyond a total of 14 years from the
product’s approval date. The patent term extension period is generally one-half the time between the effective date of an
IND, and the submission date of a NDA, plus the time between the submission date of a NDA and the approval of that
application. Only one patent applicable to an approved drug is eligible for the extension and the application for extension
must be made prior to expiration of the patent. The United States Patent and Trademark Office, in consultation with the
FDA, reviews and approves the application for any patent term extension or restoration. Our primary composition of matter
patent for OCA was to expire in 2022, but in light of the U.S. marketing approval of Ocaliva for PBC in May 2016, we
applied for an extension of the patent term for this patent in the United States into 2027, which extension has been granted.
In addition, in connection with the conditional approval of Ocaliva for PBC in the European Union, we have applied for
SPC to extend the patent term for this patent in the European Union into 2027. To date, we have received grants of SPC in
Austria, Cyprus, Denmark, Finland, France, Germany, Greece, Ireland, Italy, Norway, Portugal, Spain and Sweden and we
expect to take similar actions in other jurisdictions and countries where similar regulations exist.

Data exclusivity provisions under the FDCA also can delay the submission or the approval of certain applications. The
FDCA  provides  a  five-year  period  of  non-patent  data  exclusivity  within  the  United  States  to  the  first  applicant  to  gain
approval of a NDA for a new chemical entity. A drug is considered a new chemical entity if the FDA has not previously
approved any other new drug containing the same active moiety, which is the molecule or ion responsible for the action of
the  drug  substance  as  further  defined  in  FDA  regulations.  During  the  exclusivity  period,  the  FDA  may  not  accept  for
review  an  abbreviated  new  drug  application  (“ANDA”)  or  a  505(b)(2)  NDA  for  a  drug  with  the  same  active  moiety.
However,  an  application  may  be  submitted  four  years  from  the  NDA  approval  date  if  it  contains  a  paragraph  IV
certification that a reference product patent is invalid or not infringed by the ANDA or 505(b)(2) product. The FDCA also
provides  three  years  of  marketing  exclusivity  for  a  NDA,  505(b)(2)  NDA  or  supplement  to  an  approved  NDA  if  new
clinical investigations, other than bioavailability studies, that were conducted or sponsored by the applicant are deemed by
the  FDA  to  be  essential  to  the  approval  of  the  application,  for  example,  for  new  indications,  dosages  or  strengths  of  an
existing  drug.  This  three-year  exclusivity  covers  only  the  conditions  associated  with  the  new  clinical  investigations  and
does not prohibit the FDA from approving ANDAs or 505(b)(2) NDAs for drugs containing the original active moiety for
other  conditions  of  use.  Five-year  and  three-year  exclusivity  will  not  delay  the  submission  or  approval  of  a  full  NDA;
however,  an  applicant  submitting  a  full  NDA  may  be  required  to  conduct  or  obtain  a  right  of  reference  to  all  of  the
preclinical studies and adequate and well-controlled clinical trials necessary to demonstrate safety and effectiveness.

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Pediatric Exclusivity and Pediatric Use

Under the Best Pharmaceuticals for Children Act, sponsors may obtain a six month extension of unexpired regulatory
exclusivities  and  terms  of  unexpired  Orange  Book-listed  patents  relating  to  their  drug,  if  pediatric  studies  substantially
complying with a written request are completed and submitted by the sponsor to the FDA within the statutory time frame.
We have not received such a written request from the FDA for such pediatric studies, although we may ask the FDA to
issue a written request for such studies in the future.

In addition, under the Pediatric Research Equity Act (the “PREA”), a NDA or supplement to a NDA for certain drugs
must  contain  data  to  assess  the  safety  and  effectiveness  of  the  drug  for  the  claimed  indications  in  all  relevant  pediatric
subpopulations and to support dosing and administration for each pediatric subpopulation for which the product is safe and
effective,  unless  the  sponsor  receives  a  deferral  or  waiver.  However,  the  FDA  has  recently  issued  guidance  limiting  a
sponsor’s ability to waive the PREA study requirements.

Orphan Drug Designation

Under the Orphan Drug Act, the FDA may grant orphan drug designation to drugs intended to treat a rare disease or
condition,  which  is  generally  a  disease  or  condition  that  affects  fewer  than  200,000  individuals  in  the  United  States,  or
more  than  200,000  individuals  in  the  United  States  and  for  which  there  is  no  reasonable  expectation  that  the  cost  of
developing and making available in the United States a drug for this type of disease or condition will be recovered from
sales in the United States for that drug. Orphan drug designation must be requested before submitting a NDA. After the
FDA  grants  orphan  drug  designation,  the  identity  of  the  therapeutic  agent  and  its  potential  orphan  use  are  disclosed
publicly by the FDA. Orphan drug designation does not convey any advantage in or shorten the duration of the regulatory
review and approval process.

If a product that has orphan drug designation subsequently receives the first FDA approval for the disease for which it
has such designation, the product is entitled to orphan drug exclusivity, which means that the FDA may not approve any
applications from any other party to market the same drug for the same indication for seven years, except in very limited
circumstances such as where there is a demonstration of clinical superiority. Orphan drug exclusivity, however, could also
work to block the approval of one of our product candidates for seven years if a competitor develops the same drug as one
of  our  product  candidates  and  obtains  approval  and  orphan  exclusivity  for  the  same  indication  or  disease  for  which  our
product candidate is being developed. Orphan drug exclusivity would not block approval of the same drug developed by a
competitor for a use different from our orphan-protected approved use. If a drug or drug product designated as an orphan
product ultimately receives marketing approval for an indication broader than what was designated in its orphan product
application, it may not be entitled to orphan exclusivity for the full scope of its approved use.

As in the United States, we may apply for designation of a product as an orphan drug for the treatment of a specific
indication in the European Union before the application for marketing authorization is made. Orphan drugs in Europe enjoy
economic and marketing benefits, including up to ten years of market exclusivity for the approved indication. The market
exclusivity period for the authorized therapeutic indication may be reduced to six years if, at the end of the fifth year, it is
established  that  the  orphan  designation  criteria  are  no  longer  met,  including  where  it  is  shown  that  the  product  is
sufficiently profitable not to justify maintenance of market exclusivity. In addition, a competing similar medicinal product
may in limited circumstances be authorized prior to the expiration of the market exclusivity period, including if it is shown
to be safer, more effective or otherwise clinically superior to the orphan-designated product.

OCA has received orphan drug designation in the United States and the European Union for the treatment of PBC and
PSC. In the United States, Ocaliva has also received orphan exclusivity for its approved PBC indication that runs until May
27, 2023.

Regulation Outside of the United States

In addition to regulations in the United States, we are subject to regulations of other countries governing clinical trials
and  commercial  sales  and  distribution  of  our  products.  Whether  or  not  we  obtain  FDA  approval  for  a  product,  we  must
obtain approval by the comparable regulatory authorities of countries outside of the United States before we can commence

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clinical trials in such countries and approval of the regulators of such countries or economic areas, such as the European
Union, before we may market products in those countries or areas. The approval process and requirements governing the
conduct of clinical trials, product licensing, pricing and reimbursement vary greatly from place to place, and the time may
be longer or shorter than that required for FDA approval.

Under  European  Union  regulatory  systems,  a  company  may  submit  marketing  authorization  applications  under  the
centralized, decentralized or mutual recognition marketing authorization procedure. The centralized procedure provides for
the  grant  of  a  single  marketing  authorization  for  a  medicinal  product  by  the  European  Commission  on  the  basis  of  an
opinion provided by the EMA’s Committee for Medicinal Products for Human Use (the “CHMP”). A centralized marketing
authorization  is  valid  for  all  European  Union  member  states  and  the  European  Economic  Area  States  (Iceland,
Liechtenstein and Norway). The decentralized marketing authorization procedure involves the submission of an application
for  marketing  authorization  to  the  competent  authorities  in  each  of  the  European  Union  member  states  chosen  by  the
applicant in which the product is to be marketed. One national competent authority, selected by the applicant (Reference
Member State) leads the assessment of the application for marketing authorization. The competent authorities of the other
chosen European Union member states concerned by the procedure (Concerned Member States) are subsequently required
to review the initial evaluation and, if the assessment is positive and all issues are resolved, grant marketing authorization
for their territory on the basis of the assessment, except where grounds of potential serious risk to public health require the
application  for  authorization  to  be  refused.  The  mutual  recognition  procedure  provides  for  mutual  recognition  of  a
marketing authorization which has already been granted by the national competent authority of a European Union member
state by the competent authorities of the other European Union member states where further marketing authorizations are
progressively  sought.  The  holder  of  a  national  marketing  authorization  may  submit  an  application  to  the  competent
authority  of  a  European  Union  member  state  requesting  the  recognition  of  the  marketing  authorization  granted  by  the
competent authority of another European Union member state.

Prior to obtaining a marketing authorization in the European Union submitted as a full stand-alone dossier, applicants
have to demonstrate compliance with all measures included in an EMA-approved PIP covering all subsets of the pediatric
population, unless the EMA has granted (1) a product-specific waiver, (2) a class waiver, or (3) a deferral for one or more
of the measures included in the PIP. In the case of orphan medicinal products, completion of an approved PIP can result in
an extension of the aforementioned market exclusivity period from ten to twelve years.

It  is  also  possible  that  a  centralized  marketing  authorization  could  be  conditional  on  post-approval  studies  and  not
considered a full approval, but subject to annual renewal until comprehensive data are provided to confirm the benefit/risk
assessment.  A  manufacturer’s  ability  to  obtain  and  maintain  conditional  marketing  authorization  in  the  European  Union
will be limited to specific circumstances and subject to several conditions and obligations, if obtained at all. Conditional
marketing  authorizations  can  be  granted,  based  on  a  clinical  dataset  that  is  not  comprehensive.  Granting  of  such  an
authorization  may  be  granted  for  a  limited  number  of  medicinal  products  for  human  use  referenced  in  the  applicable
European  Union  law  governing  conditional  marketing  authorization,  including  products  designated  as  orphan  medicinal
products  under  European  Union  law,  if  (1)  the  risk-benefit  balance  of  the  product  is  positive,  (2)  it  is  likely  that  the
applicant will be in a position to provide the required comprehensive clinical trial data, (3) unmet medical needs will be
fulfilled and (4) the benefit to public health of the immediate availability on the market of the medicinal product outweighs
the  risk  inherent  in  the  fact  that  additional  data  are  still  required.  Specific  obligations,  including  with  respect  to  the
completion of ongoing or new studies, and with respect to the collection of pharmacovigilance data, may be specified in
the conditional marketing authorization. Conditional marketing authorizations are valid for one year, and may be renewed
annually,  if  the  risk-benefit  balance  remains  positive,  and  after  an  assessment  of  the  need  for  additional  or  modified
conditions.

Similarly  to  the  United  States,  both  marketing  authorization  holders  and  manufacturers  of  medicinal  products  are
subject to comprehensive regulatory oversight by the EMA and the competent authorities of the individual European Union
member  states  both  before  and  after  grant  of  the  manufacturing  and  marketing  authorizations.  This  includes  European
Union  cGMP  rules,  which  govern  quality  control  of  the  manufacturing  process  and  require  documentation  policies  and
procedures. We and our third-party manufacturers are required to ensure that all of our processes, methods, and equipment
are compliant with cGMP.

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Failure by us or by any of our third-party partners, including suppliers, manufacturers, and distributors to comply with
European Union laws and the related national laws of individual European Union member states governing the conduct of
clinical trials, manufacturing approval, marketing authorization of medicinal products and manufacturing and marketing of
such  products,  both  before  and  after  grant  of  marketing  authorization,  may  result  in  administrative,  civil  or  criminal
penalties.  These  penalties  could  include  delays  in  or  refusals  to  authorize  the  conduct  of  clinical  trials  or  the  grant  of
marketing  authorizations,  product  withdrawals  and  recalls,  product  seizures,  suspensions,  withdrawals,  or  variations  of
previously  granted  marketing  authorizations,  total  or  partial  suspensions  of  production,  distribution,  manufacturing,  or
clinical trials, operating restrictions, injunctions, suspension of licenses, fines and criminal penalties.

In  October  2016,  the  CHMP  of  the  EMA  adopted  a  positive  opinion  recommending  the  granting  of  a  conditional
marketing authorization of Ocaliva in PBC. Based on the CHMP’s positive recommendation, the European Commission
granted  a  conditional  marketing  authorization  of  Ocaliva  in  PBC  in  December  2016.  Although  we  have  successfully
renewed our conditional marketing authorization in the European Union in the past, there can be no assurance that we will
be able to continue to do so in the future. Failure to renew our conditional marketing authorization would prevent us from
continuing to market Ocaliva for PBC in Europe. PBC is not believed to occur in the pediatric population. Therefore, in
accordance  with  applicable  regulations,  the  PBC  marketing  authorization  required  demonstration  of  compliance  with  all
measures  included  in  an  EMA-approved  Pediatric  Investigation  Plan  for  OCA  for  the  treatment  of  biliary  atresia,  a
pediatric cholestatic disease.

Pricing and Reimbursement

Sales of our products will depend, in part, on the extent to which the costs of our products will be covered by third-
party payors, such as government healthcare programs, commercial insurance plans and managed healthcare organizations.
These third-party payors are increasingly challenging the prices charged for medical products and services. Additionally,
the containment of healthcare costs has become a priority for federal and state governments and the prices of drugs have
been a focus in this effort. The U.S. government, state legislatures and foreign governments have shown significant interest
in implementing cost-containment programs, including price controls, restrictions on reimbursement and requirements for
substitution of generic products. Adoption of new or more restrictive price controls and cost-containment measures in the
jurisdictions in which we operate could materially and adversely impact our net sales and financial results.

Third-party  payers  are  responsible  for  managing  overall  pharmaceutical  drug  spending  for  their  client  membership.
Third-party  payers  continue  to  scrutinize  and  manage  the  prices  charged  for  pharmaceutical  products  and  services,  and
many also limit reimbursement for newly-approved or innovating products and indications. If these third-party payors do
not consider our products to be cost-effective compared to other therapies, they may (i) not cover our approved products as
part of their plans’ benefits, (ii) apply utilization management restrictions or high patient cost-sharing obligations or (iii)
restrict  the  level  of  reimbursement  for  our  approved  products  and  any  such  actions  may  affect  our  ability  to  sell  our
approved products on a profitable basis or at all.

Medicare  is  a  U.S.  federal  healthcare  program  that  provides  coverage  for  certain  healthcare  items  and  services  to
individuals aged 65 years or older, as well as individuals of any age with certain disabilities and illnesses. The Medicare
Prescription Drug, Improvement, and Modernization Act of 2003 (“MMA”) imposed new requirements for the distribution
and pricing of prescription drugs for Medicare beneficiaries. Under Part D of the MMA, Medicare beneficiaries may enroll
in prescription drug plans offered by private entities which provide coverage for outpatient prescription drugs. Part D plans
include  both  stand-alone  prescription  drug  benefit  plans  and  prescription  drug  coverage  as  part  of  Medicare  Advantage
plans.  Unlike  Medicare  Part  A  and  B,  Part  D  prescription  drug  plan  sponsors  are  not  required  to  pay  for  all  outpatient
drugs, and each Part D plan can develop its own drug formulary that identifies which drugs it will cover and at what tier or
level. However, Part D plan drug formularies must include at least two drugs within each therapeutic category and class of
Part D drugs, though not necessarily all the drugs in each category or class. Any formulary used by a Part D prescription
drug  plan  must  be  developed  and  reviewed  by  a  pharmacy  and  therapeutics  committee.  Part  D  plan  coverage  and
reimbursement  may  increase  demand  for  our  products  for  which  we  receive  marketing  approval  in  the  United  States.
Moreover,  while  Part  D  provides  prescription  drug  benefits  only  to  Medicare  beneficiaries,  private  payors  often  follow
Medicare coverage policy and payment limitations in setting their own payment rates. Any reduction in reimbursement by
Medicare  may  result  in  a  similar  reduction  in  payments  from  non-governmental  payors.  Medicare  Part  D  may  affect
reimbursement of our products upon approval.

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Medicaid is a U.S. healthcare program that provides coverage for certain healthcare items and services to low-income
children, families, pregnant women and people with disabilities. It is jointly funded by the federal and state governments,
and it is administered by individual states within parameters established by the federal government. Therefore, coverage
and  reimbursement  for  drugs  may  vary  by  state  Medicaid  program.  A  manufacturer  must  enter  into  a  Medicaid  Drug
Rebate  Agreement  to  have  its  products  covered  by  Medicaid.  Under  the  Medicaid  program,  and  per  the  Medicaid  Drug
Rebate  Agreement,  manufacturers  agree  to  report  certain  prices  to  the  government  and  pay  rebates  to  state  Medicaid
programs based on Medicaid utilization of the manufacturer’s covered drugs.

In addition to the Medicaid Drug Rebate Program, federal law requires companies to participate in the Public Health
Service’s 340B Drug Pricing Program in order to have the manufacturer’s drugs covered under Medicaid. The 340B Drug
Pricing Program requires participating manufacturers to charge statutorily-defined covered entities no more than the 340B
“ceiling  price”  for  the  manufacturer’s  covered  outpatient  drugs.  The  Patient  Protection  and  Affordable  Care  Act,  as
amended by the Health Care and Education Affordability Reconciliation Act of 2010 (collectively, the “ACA”), extended
eligibility  to  participate  in  the  340B  program  to  certain  additional  types  of  hospitals  (including  critical  access  hospitals,
sole  community  hospitals,  rural  referral  centers  and  freestanding  cancer  hospitals).  For  purposes  of  these  newly  eligible
covered entities, the ACA specifically excluded from the definition of “covered outpatient drugs” certain drugs designated
as  “orphan  drugs”  under  section  526  of  the  FDCA.  We  are  also  required  as  a  condition  of  Medicaid  participation  to
discount our products to authorized users of the Federal Supply Schedule of the General Services Administration, including
the TRICARE retail pharmacy program, under which additional laws and requirements apply.

These  programs  require  submission  of  pricing  data  and  calculation  of  discounts  and  rebates  pursuant  to  complex
statutory formulas, and the guidance governing such calculations is not always clear. Compliance with such requirements
can  require  significant  investment  in  personnel,  systems  and  resources,  but  failure  to  properly  calculate  prices,  or  offer
required discounts or rebates can subject manufacturers to substantial penalties.

In  2010,  the  ACA  was  enacted  to,  among  other  things,  expand  access  and  increase  consumer  insurance  protections
while reducing the cost of health care for consumers. The law substantially changed the way health care is financed by both
governmental and private insurers in the United States. The ACA requires manufacturers to provide discounts on the prices
of  brand  named  drugs  in  the  coverage  gap  under  Medicare  Part  D  and  increased  the  rebates  paid  by  pharmaceutical
companies on drugs covered by Medicaid. The ACA also imposes an annual fee, which increases each year, on sales by
branded pharmaceutical manufacturers. Since its enactment, there have been a number of judicial, executive and legislative
challenges to the ACA, including tax legislation that removed the financial penalties for people who do not carry health
insurance (known as the “individual mandate”) and an Executive Order signed in October 2017 by former President Trump
directing federal agencies to modify how the ACA is implemented. Congress may continue to consider legislation to repeal
and replace some or all elements of the ACA. Further, in December 2018, a federal district court in Texas ruled that the
entire  ACA  was  unconstitutional  because  it  could  not  be  considered  an  exercise  of  Congressional  taxing  authority
following the repeal of the individual mandate penalties. In December 2019, a federal court of appeals upheld the district
court's decision that the ACA individual mandate was unconstitutional absent financial penalties, but remanded the case
back to the district court to determine whether the remaining provisions of the ACA were nonetheless valid. However, in
March  2020,  before  the  district  court  could  rule  on  the  ACA’s  remaining  provisions,  the  U.S.  Supreme  Court  agreed  to
review  the  case  and  oral  arguments  were  held  in  November  2020.  A  decision  is  expected  before  June  2021.  We  cannot
predict the outcome of this, or any other, litigation regarding the ACA or the impact it may have on our business.

There has been particular and increasing legislative and enforcement interest in the United States with respect to drug
pricing practices, particularly with respect to drugs that have been subject to relatively large price increases over relatively
short time periods. At the federal level, there have been several U.S. Congressional inquiries, proposed bills, and proposed
administrative  rules  designed  to,  among  other  things,  bring  more  transparency  to  drug  pricing,  review  the  relationship
between  pricing  and  manufacturer  patient  programs,  and  reform  government  program  reimbursement  methodologies  for
drugs. The outcome and potential effects of these proposals, and other proposals that may be forthcoming is unclear. At the
state  level,  legislatures  have  increasingly  passed  legislation  and  implemented  regulations  designed  to  control
pharmaceutical and biological product pricing, including price or patient reimbursement constraints, discounts, restrictions
on  certain  product  access  and  marketing  cost  disclosure  and  transparency  measures,  and,  in  some  cases,  to  encourage
importation from other countries and bulk purchasing.

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In addition, in some non-U.S. jurisdictions, the proposed pricing for a drug must be approved before its cost may be
funded  within  the  respective  national  healthcare  systems.  The  requirements  governing  drug  pricing  vary  widely  from
country  to  country.  For  example,  European  Union  member  states  can  restrict  the  range  of  medicinal  products  for  which
their national health insurance systems provide reimbursement and may control the prices of medicinal products for human
use. A member state may approve a specific price for the medicinal product or it may instead adopt a system of direct or
indirect controls on the profits the medicinal product generates for the company placing it on the market. There can be no
assurance  that  any  country  that  has  price  controls  or  reimbursement  limitations  for  pharmaceutical  products  will  allow
favorable  reimbursement  and  pricing  arrangements  for  any  of  our  products  on  cost-effectiveness  grounds.  Historically,
products  launched  in  countries  in  the  European  Union  do  not  follow  price  structures  of  the  United  States  and  generally
their prices tend to be significantly lower.

U.S. Fraud and Abuse Laws

Interactions and arrangements with third-party payors, healthcare providers and professionals and customers, including
patients  and  patient  advocacy  groups,  are  subject  to  broadly  applicable  fraud  and  abuse  and  other  healthcare  laws  and
regulations  that  may  restrict  certain  marketing  and  contracting  practices.  These  laws  include,  federal  and  state  anti-
kickback and false claims statutes as well as other statutes and regulations pertaining to healthcare fraud and abuse. Other
pharmaceutical companies have settled alleged or admitted violations of these fraud and abuse laws with state and federal
authorities in recent years and in some cases these settlements have amounted to hundreds of millions, or even billions, of
dollars in damages, fines, and penalties, as well as the imposition of compliance program obligations through Corporate
Integrity  Agreements  and  other  means.  Lawsuits,  or  enforcement  actions  brought  under  fraud  and  abuse  laws,  can  be
extremely  costly  to  defend,  even  if  a  company  has  strong  defenses  and  ultimately  succeeds  in  getting  the  allegations  or
enforcement action dismissed.

The federal Anti-Kickback Statute (42 U.S.C. §1320a-7b(b)) prohibits, among other things, knowingly and willfully
soliciting, receiving, offering or providing remuneration, directly or indirectly, to induce either the referral of an individual,
or the furnishing, recommending, or arranging for any good or service, for which payment may be made under federal and
state  healthcare  programs  such  as  Medicare,  Medicaid  or  other  federally  financed  healthcare  programs.  Remuneration  is
not  defined  in  the  federal  Anti-Kickback  Statute  and  has  been  broadly  interpreted  by  regulators  to  include  for  example,
cash payments, gifts, discounts, coupons, and the furnishing of free or discounted services or supplies, and other items or
services  of  value  to  the  recipient.  This  statute  has  been  broadly  interpreted  to  apply  to  manufacturer  arrangements  with
prescribers,  purchasers,  formulary  managers  and  patients,  among  others.  Although  there  are  a  number  of  statutory
exceptions and regulatory safe harbors protecting certain common activities from prosecution or other regulatory sanctions,
the  exceptions  and  safe  harbors  are  drawn  narrowly,  and  practices  that  involve  remuneration  intended  to  induce
prescribing, purchases or recommendations may be subject to scrutiny if they do not qualify for such exceptions or safe
harbors.

The  federal  False  Claims  Act  imposes  civil  penalties,  including  treble  damages  and  significant  per-claim  penalties,
which  may  be  pursued  through  civil  whistleblower  or  qui  tam  actions,  against  individuals  or  entities  for  knowingly
presenting, or causing to be presented, to the federal government, claims for payment that are false or fraudulent or making
a false statement to avoid, decrease or conceal an obligation to pay money to the federal government. The government and
qui tam relators have brought False Claims Act actions against pharmaceutical companies on the theory that their practices
have  caused  false  claims  to  be  presented  to  the  government.  There  is  also  a  separate  false  claims  provision  imposing
criminal penalties.

Other  federal  healthcare  fraud-related  laws  also  impose  criminal  liability  for  violations.  The  Criminal  Healthcare
Fraud statute (18 U.S.C. §1347) prohibits knowingly and willfully executing a scheme to defraud any healthcare benefit
program,  including  private  third-party  payers.  Federal  criminal  law  also  prohibits  knowingly  and  willfully  falsifying,
concealing or covering up a material fact or making any materially false, fictitious or fraudulent statement in connection
with the delivery of or payment for healthcare benefits, items or services.

A number of states also have statutes or regulations similar to the federal Anti-Kickback Statute and False Claims Act
that  apply  to  items  and  services  reimbursed  under  Medicaid  and  other  state  programs.  Some  state  anti-kickback  statutes
apply not just to government payors, but to all payors, including commercial payors and patients.

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Other Laws

The Health Insurance Portability and Accountability Act of 1996, as amended by the Health Information Technology
for Economic and Clinical Health Act (collectively, “HIPAA”), imposes obligations, on “covered entities,” including health
plans  and  healthcare  providers,  and  their  business  associates  with  respect  to  safeguarding  the  privacy,  security  and
transmission  of  individually  identifiable  health  information.  Although  drug  manufacturers  are  not  directly  subject  to
HIPAA, we could be subject to criminal penalties if we knowingly obtain individually identifiable health information from
a HIPAA-covered entity in a manner that is not authorized or permitted by HIPAA. We are also subject to state, federal and
international privacy and security laws governing the processing and security of personal identifiable information.

The federal Physician Payments Sunshine Act requirements under the ACA, and its implementing regulations, require
manufacturers  of  drugs,  devices,  biologics  and  medical  supplies  to  report  to  the  U.S.  Department  of  Health  and  Human
Services information related to certain direct and indirect payments and other transfers of value made to covered recipients,
such  as  physicians  and  teaching  hospitals,  as  well  as  ownership  and  investment  interests  held  by  physicians  and  their
immediate family members. Payments made to physicians and research institutions for clinical trials are included within
the ambit of this law. We are also subject to similar laws in several states and various European Union countries where we
have operations. Some of these state and EU laws are broader in scope than federal laws.

In addition, several states now require prescription drug companies to report expenses relating to the marketing and
promotion of drug products. Several states prohibit providing certain payments or items of value to healthcare providers or
other  enumerated  individuals  or  entities,  as  well  as  various  other  marketing-related  activities.  Certain  states  require  the
posting  of  information  relating  to  clinical  studies  and  their  outcomes.  In  addition,  California,  Connecticut,  Nevada  and
Massachusetts  require  pharmaceutical  companies  to  implement  compliance  programs  and  marketing  codes.  Several
additional  states  are  considering  similar  proposals.  Some  of  the  state  laws  are  broader  in  scope  than  federal  laws.
Compliance with these laws is challenging and requires significant time and resources, and any failure to comply with such
laws could result in significant civil penalties and other adverse consequences.

Human Capital Resources

As  of  December  31,  2020,  we  had  498  employees,  of  which  359  were  based  in  the  United  States,  including  at  our
facilities in New York and San Diego, and 139 were based outside the United States, including at our offices in London. A
significant percentage of our employees have obtained advanced degrees in their professions. We consider the intellectual
capital  of  our  employees  to  be  an  essential  driver  of  our  business  and  key  to  our  future  prospects.  Given  our  unique
opportunity as a leader in the treatment of progressive non-viral liver disease coupled with our disciplined management of
our financial resources, we continue to be able to fill the vacated positions and, if needed, grow our headcount in support of
our commercial organization and our pipeline of research and development programs and product candidates. We monitor
our  compensation  programs  closely  and  provide  what  we  consider  to  be  a  very  competitive  mix  of  compensation  and
insurance  benefits  for  all  our  employees,  as  well  as  participation  in  our  equity  programs.  None  of  our  employees  is
represented by a labor union and we consider our employee relations to be good. In addition, we continually evaluate our
headcount with respect to our business needs and opportunities and seek to balance in house expertise and capacity with
outsourced expertise and capacity. In August 2020, we adopted a plan to reduce our workforce in light of the receipt of the
CRL from the FDA regarding our NDA for OCA for liver fibrosis due to NASH (the “2020 Workforce Plan”). The 2020
Workforce Plan sought to streamline our operations and reduce operating expenses, while maintaining the critical resources
needed to continue to support the NASH and PBC clinical programs, pursue the approval of OCA for the treatment of liver
fibrosis due to NASH and support our successful PBC business.

Corporate and Available Information

We were incorporated in Delaware in September 2002. Our principal executive offices are located at 10 Hudson Yards,
37th  Floor,  New  York,  NY  10001  and  our  telephone  number  is  (646)  747-1000.  We  have  several  additional  offices,
including  those  in  San  Diego,  California  and  London,  United  Kingdom.  Our  corporate  website  address  is
www.interceptpharma.com.  We  make  available  on  our  website,  free  of  charge,  our  Annual  Reports  on  Form  10-K,
Quarterly Reports on Form 10-Q, Current Reports on Form 8-K and any amendments to those reports filed or furnished
pursuant to Section 13(a) or 15(d) of the Securities Exchange Act of 1934, as amended (the “Exchange Act”), as soon as

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reasonably  practicable  after  we  electronically  file  such  material  with,  or  furnish  it  to,  the  Securities  and  Exchange
Commission (“SEC”). Our SEC reports can be accessed through the Investors & Media section of our internet website. The
references  to  www.interceptpharma.com  herein  are  inactive  textual  references  only,  and  the  information  found  on  our
internet website is not incorporated by reference into this Annual Report on Form 10-K or any other report we file with or
furnish  to  the  SEC.  The  SEC  maintains  an  internet  website  that  contains  reports,  proxy  and  information  statements  and
other information about issuers, like us, that file electronically with the SEC. The address of that site is http://www.sec.gov.

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Item 1A.  Risk Factors

Investing in our securities involves a high degree of risk. The following risk factors and other information included in
this Annual Report on Form 10-K should be carefully considered before deciding whether to invest in our securities. The
risks  and  uncertainties  described  below  and  in  our  other  filings  are  not  the  only  ones  we  face.  Additional  risks  and
uncertainties not presently known to us or that we presently deem less significant may also impair our business operations.
If  any  of  the  following  risks,  or  such  unknown  risks,  occur,  our  business,  financial  condition,  results  of  operations  and
future growth prospects could be materially and adversely affected. In that case, the market price of our securities could
decline, and you may lose all or part of your investment.

Risks Related to Our Financial Position and Need for Additional Capital

We  are  currently  dependent  on  the  successful  commercialization  of  Ocaliva  for  PBC.  To  the  extent  Ocaliva  is  not
commercially  successful,  our  business,  financial  condition  and  results  of  operations  may  be  materially  and  adversely
affected and the price of our common stock may decline.

Ocaliva is our only drug that has been approved for sale and it has only been approved for the treatment of PBC in
combination with UDCA in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate
UDCA.

Our ability to generate profits from operations and become profitable currently depends on the commercial success of
Ocaliva for PBC. However, the successful commercialization of Ocaliva for PBC is subject to many risks. We have not
launched or commercialized a drug before Ocaliva, and there is no guarantee that we will be able to do so successfully.
There  are  numerous  examples  of  unsuccessful  product  launches  and  commercial  efforts,  as  well  as  failures  to  meet
expectations of market potential, including by pharmaceutical companies with greater experience and resources than us.

The commercial success of Ocaliva for PBC depends on the extent to which patients, physicians and payers accept and
adopt Ocaliva as a treatment for PBC, and we do not know whether our or others’ estimates in this regard will be accurate.
As such, there is significant uncertainty in the degree of market acceptance that Ocaliva will have for PBC. For example, if
the  patient  population  suffering  from  PBC  is  smaller  than  we  estimate,  or  even  if  the  patient  population  matches  our
estimates but Ocaliva is not widely accepted as a treatment for PBC, the commercial potential of Ocaliva for PBC will be
limited. Physicians may not prescribe Ocaliva and patients may be unwilling to use Ocaliva if coverage is not provided or
reimbursement is inadequate to cover a significant portion of the cost. In the fourth quarter of 2020, we continued to see a
lower  level  of  prescriptions  for  new  patients  than  we  did  prior  to  the  outbreak  of  COVID-19  and  related  public  health
safety  measures.  While  the  future  impact  of  COVID-19,  the  governmental  responses  thereto  and  the  resulting  rate  of
prescriptions for new patients remains difficult to predict, we did see some improvement in the fourth quarter relative to the
third quarter. We continue to monitor the situation; if the rate of prescriptions for new patients declines in the future, we
may see a reduction in net sales of Ocaliva, which could negatively affect our business, financial condition and results of
operations. Additionally, the use of Ocaliva in a non-trial setting may result in the occurrence of unexpected or a greater
incidence of side effects, adverse reactions or misuse that may negatively affect the commercial prospects of Ocaliva for
PBC. Furthermore, any negative development in any other development program for OCA or our failure to satisfy the post-
marketing regulatory commitments and requirements to which we are or may become subject, including the completion of
our Phase 4 COBALT trial, may materially and adversely impact the commercial results and potential of Ocaliva for PBC.
See  “—Risks  Related  to  the  Development  and  the  Regulatory  Review  and  Approval  of  Our  Products  and  Product
Candidates” and “—Risks Related to the Commercialization of Our Products” below.

As a result, it is uncertain whether Ocaliva net sales for PBC will sustain our operations and it may take a significant
amount of time before Ocaliva net sales for PBC sustain our operations. Furthermore, Ocaliva may not receive regulatory
approval for PBC in jurisdictions beyond those in which it is currently approved, which may also limit our prospects. If the
commercialization of Ocaliva for PBC is unsuccessful or perceived to be unsuccessful, the long-term prospects of Ocaliva
for PBC, as well as the long-term prospects of our company, may be materially and adversely affected.

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We  have  never  been  profitable.  We  expect  to  incur  losses  for  the  foreseeable  future,  and  we  may  never  achieve  or
sustain profitability.

We have never been profitable and do not expect to be profitable in the foreseeable future. We incurred net losses of
$274.9 million, $344.7 million and $309.2 million for the years ended December 31, 2020, 2019 and 2018, respectively. To
date, we have financed our operations primarily through public offerings and private placements of our securities, sales of
product  and  payments  received  under  licensing  and  collaboration  agreements.  At  December  31,  2020,  we  had  $477.2
million in cash, cash equivalents, restricted cash and investment debt securities.

We have devoted substantially all of our resources to the development of our product candidates, including the conduct
of our clinical trials, the launch and commercialization of Ocaliva for PBC, preparation for a potential launch of OCA for
liver fibrosis due to NASH and general and administrative operations, including the protection of our intellectual property.

We  expect  to  continue  to  incur  losses  for  the  foreseeable  future,  and  we  expect  these  losses  to  be  significant  as  we,
among other things, develop and seek regulatory approval for our product candidates, including OCA for liver fibrosis due
to  NASH,  maintain  our  regulatory  approvals  and  commercialize  our  approved  products.  We  believe  our  prospects  and
ability to significantly grow revenues will be dependent on our ability to successfully develop and commercialize OCA for
indications  other  than  PBC,  such  as  NASH.  As  a  result,  we  expect  a  significant  amount  of  resources  to  continue  to  be
devoted to our development programs for OCA.

As part of our product development activities, we currently expect to continue our Phase 3 clinical program of OCA for
liver fibrosis due to NASH, including our Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH through
clinical outcomes for verification and description of clinical benefit and our Phase 3 REVERSE trial for NASH patients
with compensated cirrhosis. Our expenses could increase if we are required by the FDA or the EMA to perform studies or
trials in addition to those currently expected, if our current trials are modified for any reason, or if there are any issues or
delays  in  completing  our  clinical  trials  or  the  development  of  any  of  our  product  candidates,  due  to  COVID-19  or
otherwise.  For  example,  in  June  2020  we  received  a  CRL  from  the  FDA  with  respect  to  our  NDA  for  OCA  for  liver
fibrosis due to NASH. The CRL indicated that, based on the data the FDA had reviewed, the FDA has determined that the
predicted  benefit  of  OCA  based  on  a  surrogate  histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing
REGENERATE trial in support of potential accelerated approval and that the long-term outcomes phase of the trial should
continue.  Although  we  are  in  discussions  with  the  FDA  with  respect  to  the  potential  resubmission  of  our  NDA  seeking
accelerated  approval  of  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH,  there  is  no  assurance  that  we  will  be
successful or that OCA will be approved for liver fibrosis due to NASH on an accelerated basis, or at all. Accordingly, our
previously  anticipated  U.S.  commercial  launch  of  OCA  for  liver  fibrosis  due  to  NASH  has  been  postponed,  we  do  not
expect to generate revenues for this indication until it has been approved, and we may incur significantly greater costs than
previously anticipated in connection with the development of OCA for liver fibrosis due to NASH.

We intend to continue to develop OCA and our other existing product candidates, alone or in combination, for non-viral
liver diseases. If OCA or any of our other product candidates fails in clinical trials or does not gain or maintain regulatory
approval, or if OCA or any of our other product candidates does not achieve market acceptance, we may never become
profitable.  Our  net  losses  and  negative  cash  flows  have  had,  and  will  continue  to  have,  an  adverse  effect  on  our
stockholders’ equity and working capital. Because of the numerous risks and uncertainties associated with pharmaceutical
product development and commercialization, we are unable to predict with certainty the timing or amount of our expenses,
whether such expenses may increase, or when, or if, we will be able to achieve profitability. The amount of our future net
losses will depend, in part, on our future expenses, whether and by how much such expenses increase and our ability to
generate revenues.

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We  will  require  substantial  additional  funding,  which  may  not  be  available  to  us  on  acceptable  terms,  if  at  all.  If
adequate funds are not available to us, we may be required to delay, limit, reduce or cease our operations.

We are currently developing OCA for additional indications, including NASH, and other product candidates through
various  stages  of  clinical  and  preclinical  development.  Developing  pharmaceutical  products,  including  conducting
preclinical studies and clinical trials, is expensive. If, for example, the FDA, EMA or other regulatory authorities require
that we perform additional studies beyond those that we currently expect, our expenses could increase materially beyond
what we currently anticipate, and the timing of any potential product approval may be delayed.

In  addition,  we  have  incurred  and  anticipate  that  we  will  continue  to  incur  significant  research  and  development,
product sales, marketing, manufacturing and distribution expenses relating to the commercialization of Ocaliva for PBC.
As part of our longer-term strategy, we anticipate that we will incur significant expenses in connection with our research
and  development  efforts,  the  commercialization  of  our  other  products  such  as  OCA  for  liver  fibrosis  due  to  NASH,  if
approved, and the build-out of our general and administrative infrastructure in the United States and abroad. We may also
engage  in  business  development  activities  that  involve  potential  in-  or  out-licensing  of  products  or  technologies  or
acquisitions of other products, technologies or businesses.

As  of  December  31,  2020,  we  had  $477.2  million  in  cash,  cash  equivalents,  restricted  cash  and  investment  debt
securities. We currently expect to continue to incur significant operating expenses in the fiscal year ending December 31,
2020. These expenses are planned to support, among other initiatives, the continued commercialization of Ocaliva for PBC
in the United States and our other markets, our continued clinical development of OCA for PBC and NASH and our other
earlier stage research and development programs. Although we believe that our existing capital resources, together with our
net sales of Ocaliva for PBC, will be sufficient to fund our anticipated operating requirements for the next twelve months,
we may need to raise additional capital to fund our operating requirements beyond that period. Furthermore, in light of our
receipt in June 2020 of a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to NASH and the
numerous risks and uncertainties associated with pharmaceutical product development and commercialization, any delays
in,  or  unanticipated  costs  associated  with,  our  development,  regulatory  or  commercialization  efforts  could  significantly
increase the amount of capital required by us to fund our operating requirements. Accordingly, we may seek to access the
public  or  private  capital  markets  whenever  conditions  are  favorable,  even  if  we  do  not  have  an  immediate  need  for
additional capital at that time.

Our forecasts regarding the period of time that our existing capital resources will be sufficient to meet our operating
requirements  and  the  timing  of  our  future  funding  requirements,  both  near  and  long-term,  will  depend  on  a  variety  of
factors, many of which are outside of our control. Such factors include, but are not limited to:

● our ability to successfully commercialize Ocaliva for PBC;

● our  ability  to  maintain  our  regulatory  approval  of  Ocaliva  for  PBC  in  the  United  States,  Europe,  Canada,

Israel, Australia and other jurisdictions in which we have or may receive marketing authorization;

● our ability to timely and cost-effectively file for and obtain regulatory approval of our product candidates on
an accelerated basis or at all, including OCA for liver fibrosis due to NASH following the issuance of the
CRL  by  the  FDA;  any  advisory  committee  recommendation  or  dispute  resolution  determination  that  our
product candidates, including OCA for liver fibrosis due to NASH, should not be approved or approved only
under  certain  conditions;  or  any  future  determination  that  the  regulatory  applications  and  subsequent
information  we  submit  for  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  do  not
contain adequate clinical or other data or meet applicable regulatory requirements for approval;

● conditions that may be imposed by regulatory authorities on our marketing approvals for our products and
product candidates, including OCA for liver fibrosis due to NASH, such as the need for clinical outcomes
data (and not just results based on achievement of a surrogate endpoint), any risk mitigation programs such
as  a  REMS,  and  any  related  restrictions,  limitations  and/or  warnings  contained  in  the  label  of  any  of  our
products or product candidates;

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● any potential side effects associated with Ocaliva for PBC, OCA for liver fibrosis due to NASH or our other
product candidates that could delay or prevent approval, require that an approved product be taken off the
market, require the inclusion of safety warnings or precautions or otherwise limit the sale of such product or
product candidate, including in connection with the NISS relating to Ocaliva identified by the FDA in May
2020;

● the  initiation,  timing,  cost,  conduct,  progress  and  results  of  our  research  and  development  activities,
preclinical studies and clinical trials, including any issues, delays or failures in identifying patients, enrolling
patients,  treating  patients,  retaining  patients,  meeting  specific  endpoints  in  the  jurisdictions  in  which  we
intend to seek approval or completing and timely reporting the results of our NASH or PBC clinical trials;

● the outcomes of ongoing discussions with the FDA and the EMA regarding the feasibility of the COBALT

and 401 trials;

● our ability to establish and maintain relationships with, and the performance of, third-party manufacturers,
contract  research  organizations  and  other  vendors  upon  whom  we  are  substantially  dependent  for,  among
other things, the manufacture and supply of our products, including Ocaliva for PBC and, if approved, OCA
for liver fibrosis due to NASH, and our clinical trial activities;

● our  ability  to  identify,  develop  and  successfully  commercialize  our  products  and  product  candidates,

including our ability to successfully launch OCA for liver fibrosis due to NASH, if approved;

● our  ability  to  obtain  and  maintain  intellectual  property  protection  for  our  products  and  product  candidates,
including  our  ability  to  cost-effectively  file,  prosecute,  defend  and  enforce  any  patent  claims  or  other
intellectual property rights;

● the  size  and  growth  of  the  markets  for  our  products  and  product  candidates  and  our  ability  to  serve  those

markets;

● the degree of market acceptance of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH or

our other product candidates among physicians, patients and healthcare payors;

● the  availability  of  adequate  coverage  and  reimbursement  from  governmental  and  private  healthcare  payors
for our products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH, and our
ability to obtain adequate pricing for such products;

● our ability to establish and maintain effective sales, marketing and distribution capabilities, either directly or

through collaborations with third parties;

● competition from existing drugs or new drugs that become available;

● our ability to prevent system failures, data breaches or violations of data protection laws;

● costs  and  outcomes  relating  to  any  disputes,  governmental  inquiries  or  investigations,  regulatory
proceedings,  legal  proceedings  or  litigation,  including  any  securities,  intellectual  property,  employment,
product liability or other litigation;

● our collaborators’ election to pursue research, development and commercialization activities;

● our  ability  to  establish  and  maintain  relationships  with  collaborators  with  development,  regulatory  and

commercialization expertise;

● our need for and ability to generate or obtain additional financing;

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● our estimates regarding future expenses, revenues and capital requirements and the accuracy thereof;

● our use of cash and short-term investments;

● our ability to acquire, license and invest in businesses, technologies, product candidates and products;

● our ability to attract and retain key personnel to manage our business effectively;

● our ability to manage the growth of our operations, infrastructure, personnel, systems and controls;

● our ability to obtain and maintain adequate insurance coverage;

● the  impact  of  COVID-19,  including  any  impact  on  our  results  of  operations  or  financial  position,  related
quarantines and government actions, delays relating to our regulatory applications, disruptions relating to our
ongoing clinical trials or involving our contract research organizations, study sites or other clinical partners,
disruptions  relating  to  our  supply  chain  or  involving  our  third-party  manufacturers,  distributors  or  other
distribution partners, facility closures or other restrictions, and the extent and duration thereof;

● the  impact  of  general  U.S.  and  foreign  economic,  industry,  market,  regulatory  or  political  conditions,

including the potential impact of Brexit; and

● the other risks and uncertainties identified under the captions “Risk Factors” and “Management’s Discussion
and  Analysis  of  Financial  Condition  and  Results  of  Operations”  and  elsewhere  in  this  Annual  Report  on
Form 10-K and in our other periodic filings filed with the SEC.

We have no committed external sources of funding and additional funds may not be available when we need them on
terms that are acceptable to us, or at all. In addition, in recent months global markets have experienced significant volatility
in connection with concerns over the impact of COVID-19, and such concerns may in the future materially and adversely
affect  our  ability  to  raise  funds.  If  adequate  funds  are  not  available  to  us,  we  may  not  be  able  to  make  scheduled  debt
payments on a timely basis, or at all, and may be required to delay, limit, reduce or cease our operations.

Raising  additional  capital  may  cause  dilution  to  our  stockholders,  restrict  our  operations  or  require  us  to  relinquish
rights to our technologies or product candidates.

Unless  and  until  we  generate  sufficient  cash  flow  from  sales  of  our  products,  including  Ocaliva  for  PBC  and,  if
approved, OCA for liver fibrosis due to NASH, we expect to finance our future cash needs through public or private equity
or  debt  financings,  government  or  other  third-party  funding,  marketing  and  distribution  arrangements  or  other
collaborations, strategic alliances and licensing arrangements, or a combination of these sources. Additional funding may
not be available to us on acceptable terms, if at all.

The terms of any future financing may adversely affect the interests of our existing securityholders. For example, to
the  extent  that  we  raise  additional  capital  through  the  sale  of  equity  or  convertible  debt  securities,  our  stockholders’
ownership  interest  will  be  diluted,  and  the  terms  of  these  securities  may  include  liquidation  or  other  preferences  that
adversely affect the rights of our common stockholders. Debt financing, if available, may involve agreements that include
covenants  limiting  or  restricting  our  ability  to  take  specific  actions,  such  as  incurring  additional  debt,  making  capital
expenditures  or  declaring  dividends.  We  also  could  be  required  to  seek  funds  through  arrangements  with  licensing  or
collaborative  partners  or  otherwise  that  may  require  us  to  relinquish  rights  to  some  of  our  technologies  or  product
candidates or otherwise agree to terms unfavorable to us. If we are unable to raise additional funds through equity or debt
financings  when  needed,  we  may  be  required  to  delay,  limit,  reduce  or  terminate  our  product  development  or  future
commercialization  efforts  or  grant  rights  to  develop  and  market  product  candidates  that  we  would  otherwise  prefer  to
develop and market ourselves.

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We  have  a  limited  operating  history  as  a  commercial  organization,  which  may  make  it  difficult  to  predict  our  future
performance, and we expect to continue to face a number of factors that may cause operating results to fluctuate.

We  are  a  biopharmaceutical  company  with  a  limited  operating  history  as  a  commercial  organization.  Prior  to  the
launch and commercialization of Ocaliva for PBC, our operations were limited to developing our technology, undertaking
preclinical  studies  and  clinical  trials  of  our  product  candidates  and  preparing  for  the  commercial  launch  of  Ocaliva  for
PBC. Other than Ocaliva for PBC, none of our other product candidates have received regulatory approval. Consequently,
any  predictions  regarding  our  future  success  or  viability  may  not  be  as  accurate  as  they  could  be  if  we  had  a  longer
operating history or greater experience commercializing approved products.

The commercialization of Ocaliva for PBC has been and will continue to be, and, if approved, the commercialization of
OCA for liver fibrosis due to NASH will be, expensive and time-consuming, and we cannot be certain that we will be able
to generate sufficient revenues from sales of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH in our
target markets to offset such costs. Furthermore, our financial condition and operating results have varied significantly in
the past and are expected to continue to significantly fluctuate from quarter-to-quarter and year-to-year due to a variety of
factors, many of which are outside of our control. Such factors include, but are not limited to:

● our ability to successfully commercialize Ocaliva for PBC;

● our  ability  to  maintain  our  regulatory  approval  of  Ocaliva  for  PBC  in  the  United  States,  Europe,  Canada,

Israel, Australia and other jurisdictions in which we have or may receive marketing authorization;

● our ability to timely and cost-effectively file for and obtain regulatory approval of our product candidates on
an accelerated basis or at all, including OCA for liver fibrosis due to NASH following the issuance of the
CRL  by  the  FDA;  any  advisory  committee  recommendation  or  dispute  resolution  determination  that  our
product candidates, including OCA for liver fibrosis due to NASH, should not be approved or approved only
under  certain  conditions;  or  any  future  determination  that  the  regulatory  applications  and  subsequent
information  we  submit  for  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  do  not
contain adequate clinical or other data or meet applicable regulatory requirements for approval;

● conditions that may be imposed by regulatory authorities on our marketing approvals for our products and
product candidates, including OCA for liver fibrosis due to NASH, such as the need for clinical outcomes
data (and not just results based on achievement of a surrogate endpoint), any risk mitigation programs such
as  a  REMS,  and  any  related  restrictions,  limitations  and/or  warnings  contained  in  the  label  of  any  of  our
products or product candidates;

● any potential side effects associated with Ocaliva for PBC, OCA for liver fibrosis due to NASH or our other
product candidates that could delay or prevent approval, require that an approved product be taken off the
market, require the inclusion of safety warnings or precautions or otherwise limit the sale of such product or
product candidate, including in connection with the NISS relating to Ocaliva identified by the FDA in May
2020;

● the  initiation,  timing,  cost,  conduct,  progress  and  results  of  our  research  and  development  activities,
preclinical studies and clinical trials, including any issues, delays or failures in identifying patients, enrolling
patients,  treating  patients,  retaining  patients,  meeting  specific  endpoints  in  the  jurisdictions  in  which  we
intend to seek approval or completing and timely reporting the results of our NASH or PBC clinical trials;

● the outcomes of ongoing discussions with the FDA and EMA regarding the feasibility of the COBALT and

401 trials;

● our ability to establish and maintain relationships with, and the performance of, third-party manufacturers,
contract  research  organizations  and  other  vendors  upon  whom  we  are  substantially  dependent  for,  among
other things, the manufacture and supply of our products, including Ocaliva for PBC and, if approved, OCA
for liver fibrosis due to NASH, and our clinical trial activities;

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● our  ability  to  identify,  develop  and  successfully  commercialize  our  products  and  product  candidates,

including our ability to successfully launch OCA for liver fibrosis due to NASH, if approved;

● our  ability  to  obtain  and  maintain  intellectual  property  protection  for  our  products  and  product  candidates,
including  our  ability  to  cost-effectively  file,  prosecute,  defend  and  enforce  any  patent  claims  or  other
intellectual property rights;

● the  size  and  growth  of  the  markets  for  our  products  and  product  candidates  and  our  ability  to  serve  those

markets;

● the degree of market acceptance of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH or

our other product candidates among physicians, patients and healthcare payors;

● the  availability  of  adequate  coverage  and  reimbursement  from  governmental  and  private  healthcare  payors
for our products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH, and our
ability to obtain adequate pricing for such products;

● our ability to establish and maintain effective sales, marketing and distribution capabilities, either directly or

through collaborations with third parties;

● competition from existing drugs or new drugs that become available;

● our ability to prevent system failures, data breaches or violations of data protection laws;

● costs  and  outcomes  relating  to  any  disputes,  governmental  inquiries  or  investigations,  regulatory
proceedings,  legal  proceedings  or  litigation,  including  any  securities,  intellectual  property,  employment,
product liability or other litigation;

● our collaborators’ election to pursue research, development and commercialization activities;

● our  ability  to  establish  and  maintain  relationships  with  collaborators  with  development,  regulatory  and

commercialization expertise;

● our need for and ability to generate or obtain additional financing;

● our estimates regarding future expenses, revenues and capital requirements and the accuracy thereof;

● our use of cash and short-term investments;

● our ability to acquire, license and invest in businesses, technologies, product candidates and products;

● our ability to attract and retain key personnel to manage our business effectively;

● our ability to manage the growth of our operations, infrastructure, personnel, systems and controls;

● our ability to obtain and maintain adequate insurance coverage;

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● the  impact  of  COVID-19,  including  any  impact  on  our  results  of  operations  or  financial  position,  related
quarantines and government actions, delays relating to our regulatory applications, disruptions relating to our
ongoing clinical trials or involving our contract research organizations, study sites or other clinical partners,
disruptions  relating  to  our  supply  chain  or  involving  our  third-party  manufacturers,  distributors  or  other
distribution partners, facility closures or other restrictions, and the extent and duration thereof;

● the  impact  of  general  U.S.  and  foreign  economic,  industry,  market,  regulatory  or  political  conditions,

including the potential impact of Brexit; and

● the other risks and uncertainties identified under the captions “Risk Factors” and “Management’s Discussion
and  Analysis  of  Financial  Condition  and  Results  of  Operations”  and  elsewhere  in  this  Annual  Report  on
Form 10-K and in our other periodic filings filed with the SEC.

Risks Related to the Development and the Regulatory Review and
Approval of Our Products and Product Candidates

We  cannot  be  certain  whether  Ocaliva  will  receive  full  approval  for  PBC  in  jurisdictions  where  it  has  previously
received accelerated or conditional approval, or that Ocaliva will be approved for PBC in any jurisdictions beyond those
in which it is currently approved. Furthermore, OCA may not be approved on an accelerated basis, or at all, for NASH
or  any  other  indication  beyond  PBC  and  we  may  not  receive  regulatory  approval  for  any  other  product  candidate.
Without regulatory approval, we will not be able to market and commercialize our product candidates.

The  development,  testing,  manufacture,  packaging,  labeling,  storage,  approval,  promotion,  advertising,  distribution,
marketing  and  export  and  import,  among  other  things,  of  our  products  and  product  candidates  are  subject  to  extensive
regulation by the FDA in the United States, the EMA in Europe and various regulatory authorities in other countries, with
regulations differing from country to country. We are not permitted to market our product candidates in the United States or
Europe  until  we  receive  approval  of  a  NDA,  from  the  FDA,  or  a  MAA,  from  the  European  Commission,  respectively.
Currently, our ability to generate product sales depends on the successful marketing of Ocaliva for PBC in the jurisdictions
in  which  it  has  received  regulatory  approval.  In  the  future,  our  ability  to  generate  product  sales  in  addition  to  those  of
Ocaliva  for  PBC  will  depend  on  whether  we  are  successful  in  obtaining  regulatory  approval  of  our  other  product
candidates, including OCA for liver fibrosis due to NASH.

Ocaliva is our only drug that has been approved for sale and it has only been approved for the treatment of PBC in
combination with UDCA in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate
UDCA. In the United States, Ocaliva was approved for PBC under the accelerated approval pathway. Accelerated approval
was  granted  for  Ocaliva  for  PBC  based  on  a  reduction  in  ALP;  however,  an  improvement  in  survival  or  disease-related
symptoms has not yet been established. Continued approval of Ocaliva for PBC in the United States is contingent upon the
verification  and  description  of  clinical  benefit  in  confirmatory  trials  and  our  satisfaction  of  our  other  post-marketing
regulatory requirements. Any delay of the COBALT trial or failure by us to confirm the clinical benefit of Ocaliva for PBC
due  to  COVID-19  or  other  factors  may  jeopardize  the  continued  approval  of  Ocaliva  for  PBC.  As  specified  by  the
applicable post-marketing requirements, our COBALT trial includes patients across the spectrum of PBC disease, including
early and advanced PBC. We have agreed to evaluate the safety and efficacy of Ocaliva in patients with moderate to severe
hepatic impairment and as a monotherapy in patients with PBC. In addition, we agreed to develop and characterize a lower
dose formulation of Ocaliva to allow for once daily dosing in patients with moderate or advanced hepatic impairment, and
we have fulfilled this commitment.

We  commenced  our  commercial  launch  of  Ocaliva  for  PBC  in  certain  European  countries  in  2017  following  the
European  Commission’s  grant  of  conditional  approval  in  December  2016.  Our  marketing  authorization  in  the  European
Union  is  conditioned  on  the  successful  completion  of  the  COBALT  trial  and  in  our  401  trial  evaluating  the  safety  and
efficacy of Ocaliva in patients with moderate to severe hepatic impairment.

Since January 2017, Ocaliva has also received regulatory approval in several of our target markets outside the United
States and Europe, including Canada, Israel and Australia, and we are pursuing marketing approval of Ocaliva for PBC in
our other international target markets. If obtained, continued approval of Ocaliva for PBC in such jurisdictions may be

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contingent upon the verification and description of clinical benefit in confirmatory trials. Any delay or failure in satisfying
the  post-marketing  regulatory  commitments  and  requirements  to  which  we  are  or  may  become  subject,  including  our
COBALT trial, may jeopardize the continued approval of Ocaliva for PBC in the United States, European Union and other
jurisdictions. In some markets where regulatory approval has been obtained for Ocaliva, discussions with national public
health system authorities regarding reimbursement are ongoing.

While we remain blinded to safety and efficacy data in the ongoing COBALT trial and 401 trial, the DMC reviewed
the unblinded results of a pre-specified interim efficacy analysis of the COBALT trial and separately reviewed unblinded
safety and pharmacokinetic data from both the COBALT and 401 trials. Following these reviews, the DMC stated that it
was not feasible to continue the COBALT trial as designed and noted the challenges in enrolling and maintaining placebo-
controlled post-marketing studies in this rare disease setting. No acute safety concerns were noted by the DMC. Given the
feasibility  concerns  noted  by  the  DMC  as  well  as  the  potential  confounding  impact  of  subjects  discontinuing  treatment
and/or transitioning from investigational product to commercial drug during clinical trials, we continue to discuss with the
FDA and the EMA proposed modifications to the COBALT trial as well as proposals with respect to the 401 trial. We have
notified the FDA and the EMA of the DMC’s recommendation and, as they previously advised, are in ongoing discussions
with the FDA on the matter and are seeking formal EU scientific advice with respect to potential alternative study designs.
In addition, future changes to our Ocaliva label related to the most advanced PBC patients will influence the modifications
to our study design. If we are unable to satisfactorily address the data monitoring committee’s recommendation with the
FDA and/or the EMA and the COBALT trial cannot be timely completed, cannot be completed as designed or fails, we
may not be able to maintain our previously granted marketing approval of Ocaliva for PBC. Ocaliva is not approved for
any indication other than PBC. We currently have no other products approved for sale and we cannot guarantee that we will
ever have additional marketable products or that OCA will be approved for use in additional indications such as NASH.
NDAs and MAAs must include extensive preclinical and clinical data and supporting information to establish the product
candidate’s  safety  and  effectiveness  for  each  desired  indication.  NDAs  and  MAAs  must  also  include  significant
information regarding the chemistry, manufacturing and controls for the product. Obtaining approval of a NDA or a MAA
is a lengthy, expensive and uncertain process, and we may not be successful in obtaining approval. The FDA and the EMA
review processes can take years to complete and approval is not guaranteed. Even after the submission of a NDA, the FDA
may  decide  not  to  accept  the  submission  for  filing  and  review  or  may  determine  that  the  submission  does  not  support
approval. For example, in June 2020 we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis
due  to  NASH.  The  CRL  indicated  that,  based  on  the  data  the  FDA  had  reviewed,  the  FDA  had  determined  that  the
predicted  benefit  of  OCA  based  on  a  surrogate  histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing
REGENERATE  study  in  support  of  potential  accelerated  approval  and  that  the  long-term  outcomes  phase  of  the  study
should continue. Similarly, there are a number of factors that may result in delays in the EMA’s review process following
the  submission  of  a  MAA,  or  the  EMA  may  determine  that  the  submission  does  not  support  approval  on  a  conditional
basis, or at all. The United Kingdom left the European Union on January 31, 2020, in what is often referred to as “Brexit,”
and the end of the transition period was December 31, 2020. At present, the regulatory framework in the United Kingdom
is  currently  aligned  with  European  Union  directives  and  regulations.  However,  over  time,  Brexit  may  result  in  material
changes to the regulatory regime applicable to many of our current operations, including those relating to Ocaliva for PBC
and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH,  because  of  the  nature  of  the  Brexit  deal  (the  EU-UK  Trade  and
Cooperation Agreement) between the United Kingdom and the EU, such that the UK is no longer a member of the single
market or the customs union. COVID-19 could also affect the operations of the FDA, EMA and other health authorities,
which could delay our clinical development efforts and the review and approval of our product candidates, including OCA
for liver fibrosis due to NASH.

As is the case with the approval of Ocaliva for PBC, any future approvals or potential future approvals may also be
conditional upon the completion of one or more clinical trials. In addition, delays in approvals or rejections of marketing
applications  in  the  United  States,  Europe  or  other  countries  may  be  based  upon  many  factors,  including,  for  example,
regulatory  requests  for  additional  analyses,  reports,  data,  preclinical  studies  and  clinical  trials,  regulatory  endpoint
requirements,  regulatory  questions  regarding  safety  or  risk-benefit  profile,  different  interpretations  of  data  and  results,
changes in regulatory policy during the period of product development and the emergence of new information regarding
our product candidates or approved products. Initial and continued regulatory approval is also dependent on successfully
passing regulatory inspection requirements applicable to us, our clinical sites and our key vendors, including requirements

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that we and such parties comply with applicable good clinical, pharmacovigilance, laboratory and manufacturing practices
regulations.  Critical  findings  could  jeopardize  or  delay  the  approval  of  our  NDAs  or  MAAs  or  impair  our  ability  to
maintain our marketing approvals.

Prior to receiving regulatory approval, we must finalize the product label for each of our product candidates in each
jurisdiction  in  which  we  seek  regulatory  approval.  Even  if  our  product  is  approved,  the  FDA,  EMA  or  other  applicable
regulatory authorities may limit the indications or uses for which our product may be marketed, require extensive warnings
on the product labeling or require expensive and time-consuming clinical trials, risk mitigation programs such as a REMS,
monitoring or reporting as a condition of approval. Also, regulatory approval for our approved products may be withdrawn.
In addition, obtaining regulatory approval for the marketing of our product in one country does not ensure that we will be
able to obtain regulatory approval for such product in any other country.

In  order  to  obtain  and/or  maintain  regulatory  approval  for  OCA  for  indications  other  than  PBC,  we  will  need  to
complete additional clinical trials and studies. For example, in connection with our Phase 3 clinical program of OCA for
liver fibrosis due to NASH, we are currently conducting our Phase 3 REGENERATE trial in patients with liver fibrosis due
to NASH through clinical outcomes for verification and description of clinical benefit and our Phase 3 REVERSE trial for
NASH  patients  with  compensated  cirrhosis.  While  our  ongoing  Phase  3  REGENERATE  and  REVERSE  trials  are  fully
enrolled and we have taken measures intended to minimize disruptions and protect and retain patients participating in such
trials due to COVID-19, we cannot predict the degree to which such measures will ultimately prove effective. Our ability to
obtain and maintain the regulatory approvals necessary to commercialize OCA for indications other than PBC, including
NASH, will depend on our ability to successfully design, conduct and complete these trials, the efficacy, safety and risk-
benefit  profile  of  OCA  demonstrated  by  such  trials  and  our  ability  to  prepare  and  submit  complex  regulatory  filings  in
accordance with applicable regulatory requirements.

There can be no assurance that OCA will receive marketing approval on an accelerated or conditional basis, or at all,
for  PBC  in  jurisdictions  where  it  has  not  yet  been  approved  or  for  NASH  in  any  jurisdiction,  or  that  any  of  our  other
product candidates will receive marketing approval for any indication in any jurisdiction. We cannot predict whether our
clinical  trials  and  studies  for  our  product  candidates,  including  OCA  for  PBC,  NASH  or  any  other  indication,  will  be
successful,  whether  regulatory  authorities  will  agree  with  our  conclusions  relating  to  the  clinical  trials  and  studies  we
conduct, or whether such regulatory authorities will require us to conduct additional clinical trials or studies. For example,
while OCA received breakthrough therapy designation from the FDA in January 2015 for the treatment of NASH patients
with liver fibrosis and we filed a NDA in the United States and a MAA in Europe based on the results from the 18-month
analysis of our Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH, we do not know if one pivotal
clinical trial will be sufficient for marketing approval or if regulatory authorities in the United States, Europe or our other
target markets will approve OCA for liver fibrosis due to NASH on an accelerated or conditional basis, or at all. Our Phase
3 REGENERATE trial remains blinded after the interim analysis and is expected to continue to follow patients until the
occurrence of a pre-specified number of adverse clinical outcomes, including progression to cirrhosis, for verification and
description of clinical benefit.

If  we  are  unable  to  obtain  regulatory  approval  for  OCA  for  PBC  in  the  jurisdictions  in  which  it  is  not  currently
approved  or  obtain  regulatory  approval  in  the  United  States,  European  Union  and  other  jurisdictions  for  OCA  for  other
indications,  such  as  NASH,  or  for  our  other  product  candidates,  we  may  not  be  able  to  generate  sufficient  revenue  to
become profitable or to continue our operations.

We are developing product candidates for the treatment of rare diseases or diseases for which there are no or limited
therapies,  such  as  PBC  and  NASH,  and  for  some  of  which  there  is  little  clinical  experience,  and  our  development
approach involves new endpoints and methodologies. As a result, there is a heightened risk that we will not be able to
gain agreement with regulatory authorities regarding an acceptable development plan, that the outcome of our clinical
trials will not be favorable or that, even if favorable, regulatory authorities may not find the results of our clinical trials
to be sufficient for marketing approval.

We are focused on developing therapeutics for the treatment of rare diseases and diseases for which there are no or
limited treatments. As a result, the design and conduct of our clinical trials for these indications is subject to heightened
risk.

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In the United States, the FDA generally requires two adequate and well-controlled pivotal clinical trials to approve a
NDA. Furthermore, for full approval of a NDA, the FDA requires a demonstration of efficacy based on a clinical benefit
endpoint.  The  FDA  may  grant  accelerated  approval  based  on  a  surrogate  endpoint  reasonably  likely  to  predict  clinical
benefit. Even though our pivotal clinical trials for a specific indication, such as our Phase 3 REGENERATE trial of OCA in
patients with liver fibrosis due to NASH and our Phase 3 REVERSE trial for NASH patients with compensated cirrhosis,
may achieve their primary endpoints and are reasonably believed by us to be likely to predict clinical benefit, the FDA may
not accept the results of such trials or approve our product candidate on an accelerated basis, or at all. It is also possible
that the FDA may refuse to accept for filing and review any regulatory application we submit for regulatory approval in the
United States. Even if our regulatory application is accepted for review, there may be delays in the FDA’s review process
and the FDA may determine that such regulatory application does not contain adequate clinical or other data or support the
approval  of  the  product  candidate.  In  such  a  case,  the  FDA  may  issue  a  CRL  that  may  require  that  we  conduct  and/or
complete additional clinical trials and preclinical studies or provide additional information or data before it will reconsider
our application for approval. For example, in June 2020 we received a CRL from the FDA regarding our NDA for OCA for
liver fibrosis due to NASH. The CRL indicated that, based on the data the FDA had reviewed, the FDA had determined
that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing
REGENERATE  study  in  support  of  potential  accelerated  approval  and  that  the  long-term  outcomes  phase  of  the  study
should continue. The requirements imposed by the FDA may be substantial, expensive and time-consuming, and there is no
guarantee  that  we  will  continue  to  pursue  any  such  application  or  that  the  FDA  will  ultimately  decide  that  any  such
application supports the approval of the product candidate on an accelerated basis, or at all. The FDA may also refer any
regulatory application to an advisory committee for review and recommendation as to whether, and under what conditions,
the  application  should  be  approved.  While  the  FDA  is  not  bound  by  the  recommendation  of  an  advisory  committee,  it
considers such recommendations carefully when making decisions.

Even if we receive accelerated approval for any of our product candidates, we may be required to conduct or complete
a  post-approval  clinical  outcomes  trial  to  confirm  the  clinical  benefit  of  such  product  candidates  by  demonstrating  the
correlation  of  the  surrogate  endpoint  therapeutic  response  in  patients  with  a  significant  reduction  in  adverse  clinical
outcomes over time. For example, interim analysis results at 18 months in our Phase 3 REGENERATE trial were based on
surrogate endpoints and the impact on clinical outcomes has not been confirmed. The REGENERATE trial is ongoing for
verification and description of clinical benefit of OCA for liver fibrosis due to NASH. There can be no assurance that the
clinical  outcomes  portion  of  our  REGENERATE  trial  will  confirm  that  the  surrogate  endpoint  used  as  the  basis  of  the
regulatory  submissions  we  have  made  or  expect  to  make  seeking  approval  of  OCA  for  liver  fibrosis  due  to  NASH  will
eventually show an adequate correlation with clinical outcomes. In addition, as a condition of the accelerated approval of
Ocaliva  for  PBC  in  the  United  States,  we  are  required  to  conduct  a  clinical  outcomes  study  with  respect  to  Ocaliva  for
PBC. Following discussions with regulatory authorities, we initiated our COBALT clinical outcomes confirmatory trial for
PBC in December 2014 prior to the approval of Ocaliva for PBC. The COBALT trial includes subjects across the spectrum
of PBC disease, including early and advanced PBC. We have also agreed to evaluate the safety and efficacy of Ocaliva in
patients with moderate to severe hepatic impairment in the 401 trial and as a monotherapy in patients with PBC. There can
be no assurance that our COBALT trial conducted as part of our post-marketing obligations will confirm that the surrogate
endpoint  used  for  accelerated  approval  of  Ocaliva  for  PBC  will  eventually  show  an  adequate  correlation  with  clinical
outcomes or that our clinical 401 trial in PBC patients with moderate to severe hepatic impairment will be successful.

While we remain blinded to safety and efficacy data in the ongoing COBALT trial and 401 trial, the DMC reviewed
the unblinded results of a pre-specified interim efficacy analysis of the COBALT trial and separately reviewed unblinded
safety and pharmacokinetic data from both the COBALT and 401 trials. Following these reviews, the DMC stated that it
was not feasible to continue the COBALT trial as designed and noted the challenges in enrolling and maintaining placebo-
controlled post-marketing studies in this rare disease setting. No acute safety concerns were noted by the DMC. Given the
feasibility  concerns  noted  by  the  DMC  and  the  potential  confounding  impact  of  subjects  discontinuing  treatment  and/or
transitioning from investigational product to commercial drug during clinical trials, we continue to discuss with the FDA
and  the  EMA  proposed  modifications  to  the  COBALT  trial  as  well  as  proposals  with  respect  to  the  401  trial.  We  have
notified the FDA and the EMA of the DMC’s recommendation and, as they previously advised, are in ongoing discussions
with the FDA on the matter and are seeking formal EU scientific advice with respect to potential alternative study designs.

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In addition, future changes to our Ocaliva label related to the most advanced PBC patients will influence the modifications
to our study design. If we are unable to satisfactorily address the DMC’s recommendation with the FDA and/or the EMA
and  the  COBALT  trial  cannot  be  timely  completed,  cannot  be  completed  as  designed  or  fails,  we  may  not  be  able  to
maintain  our  previously  granted  marketing  approval  of  Ocaliva  for  PBC.  Similarly,  if  approved  based  on  a  surrogate
endpoint, continued approval of OCA for other indications, or of any of our other product candidates, may be contingent
upon the verification and description of clinical benefit in confirmatory trials.

Our  marketing  authorization  in  the  European  Union  for  Ocaliva  for  the  treatment  of  PBC  is  not  a  full  approval.
Instead,  it  is  conditional  on  the  conduct  of  certain  post-approval  studies,  including  the  COBALT  trial.  Our  ability  to
maintain  conditional  marketing  authorization  of  Ocaliva  for  PBC  in  the  European  Union  is  limited  to  specific
circumstances  and  subject  to  several  conditions  and  obligations  that  we  may  be  unable  to  satisfy  in  whole  or  at  all,
including  the  completion  of  one  or  more  clinical  outcomes  trials  to  confirm  the  clinical  benefit  of  Ocaliva  for  PBC.
Conditional  marketing  authorizations  based  on  incomplete  clinical  data  may  be  granted  for  a  limited  number  of  listed
medicinal products for human use, including products designated as orphan medicinal products under European Union law,
if (i) the risk-benefit balance of the product is positive, (ii) it is likely that the applicant will be in a position to provide the
required comprehensive clinical trial data, (iii) unmet medical needs will be fulfilled and (iv) the benefit to public health of
the  immediate  availability  on  the  market  of  the  medicinal  product  outweighs  the  risk  inherent  in  the  fact  that  additional
data  are  still  required.  Specific  obligations,  including  obligations  relating  to  the  timely  and  successful  completion  of
ongoing  or  new  studies  and  the  collection  of  pharmacovigilance  data,  may  be  specified  in  the  conditional  marketing
authorization. Conditional marketing authorizations are valid for one year, and may be renewed annually, if the risk-benefit
balance  remains  positive,  and  after  an  assessment  of  the  need  for  additional  or  modified  conditions.  Although  we  have
successfully renewed our conditional marketing authorization in the European Union in the past, there can be no assurance
that  we  will  be  able  to  continue  to  do  so  in  the  future.  Failure  to  renew  our  conditional  marketing  authorization  would
prevent us from continuing to market Ocaliva for PBC in Europe.

Our ongoing Phase 3 REGENERATE trial of OCA in patients with liver fibrosis due to NASH incorporates an interim
primary surrogate endpoint that may serve as the basis for accelerated approval in the United States and as the basis for a
conditional approval in Europe. Accelerated approval in the United States and conditional approval in the European Union
for OCA for liver fibrosis due to NASH are subject to similar risks as discussed above in relation to OCA for PBC. In the
REGENERATE primary efficacy analysis, once-daily OCA 25 mg met, with statistical significance, the primary endpoint
agreed with the FDA of fibrosis improvement by at least one stage with no worsening of NASH (defined as no worsening
of hepatocellular ballooning, no worsening of lobular inflammation and no worsening of steatosis) at the planned 18-month
analysis.  Although  a  numerically  greater  proportion  of  patients  in  both  OCA  treatment  groups  compared  to  placebo
achieved the primary endpoint of NASH resolution with no worsening of liver fibrosis in the primary efficacy analysis, this
result did not reach statistical significance. As agreed with the FDA, in order for the primary objective to be met, the study
was required to achieve one of the two primary endpoints. Notwithstanding the results of the REGENERATE 18-month
analysis,  the  recent  CRL  issued  by  the  FDA  indicated  that,  based  on  the  data  the  FDA  had  reviewed,  the  FDA  had
determined that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not
sufficiently outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due
to  NASH.  The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the
ongoing REGENERATE study in support of potential accelerated approval and that the long-term outcomes phase of the
study should continue. Although we are in discussions with the FDA with respect to the potential resubmission of our NDA
seeking accelerated approval of OCA for the treatment of liver fibrosis due to NASH, there is no assurance that we will be
successful or that OCA will be approved for liver fibrosis due to NASH on an accelerated basis, or at all. Furthermore, in
November 2018, the EMA issued a draft position paper in which it presented its preliminary views with respect to various
NASH  clinical  development  matters,  including  with  respect  to  potential  surrogate  endpoints,  and  requested  comments
thereon by August 2019. Although we did not reach agreement with the EMA on the definition and analysis of a surrogate
endpoint  prior  to  the  readout  of  the  18-month  analysis  of  the  REGENERATE  trial,  we  believe  that  the  totality  of  the
REGENERATE interim analysis data supports the MAA we filed with the EMA. However, the data that we have submitted
to the EMA may not ultimately be found by the EMA to be sufficient for marketing approval on a conditional basis, or at
all. In June 2019, the FDA issued new draft guidance on the development of drugs for the treatment of NASH patients with
compensated  cirrhosis.  Although  we  believe  that,  if  successful,  our  Phase  3  REVERSE  trial  will  support  a  regulatory
submission seeking accelerated approval of OCA for liver fibrosis due to NASH with compensated

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cirrhosis  in  the  U.S.,  we  do  not  know  if  achievement  of  the  primary  endpoint  will  ultimately  be  found  sufficient  by  the
FDA for approval on an accelerated basis, or at all.

While  OCA  received  breakthrough  therapy  designation  from  the  FDA  in  January  2015  for  the  treatment  of  NASH
patients with liver fibrosis and we have filed a NDA in the United States and a MAA in Europe for approval of OCA for
liver fibrosis due to NASH based on the results from the 18-month interim analysis of our Phase 3 REGENERATE trial,
we  do  not  know  if  one  pivotal  clinical  trial  will  be  sufficient  for  marketing  approval  or  if  regulatory  authorities  in  the
United States, Europe or our other target markets will approve OCA for liver fibrosis due to NASH on an accelerated or
conditional basis, or at all. There may be delays in the FDA and EMA review processes and the FDA and/or the EMA may
also require that we continue our Phase 3 REGENERATE trial until completion to assess the potential benefits of OCA
treatment on liver-related and other clinical outcomes. Our regulatory pathway for OCA for the treatment of NASH will
depend upon our discussions with the FDA and the EMA. As a result, we may face difficulty in establishing an acceptable
registration  strategy  with  respect  to  our  Phase  3  REGENERATE  and  REVERSE  trials,  as  well  as  other  trials  we  may
conduct in other subpopulations of NASH patients.

Prior  to  any  approval  of  OCA  for  liver  fibrosis  due  to  NASH  or  OCA  for  PBC  in  jurisdictions  in  which  it  is  not
currently  approved  or  the  approval  of  our  other  product  candidates,  the  FDA,  EMA  or  other  applicable  regulatory
authorities may require additional preclinical studies and/or clinical trials, which may be expensive and time consuming to
conduct and complete. Consequently, any such requirement that we conduct additional preclinical studies or clinical trials
could materially and adversely affect our business, financial condition and results of operations. Furthermore, even if we
receive  such  approval,  any  risk  mitigation  programs  such  as  a  REMS,  and  any  related  restrictions,  limitations  and/or
warnings  contained  in  the  label  of  our  approved  products  could  impact  our  commercial  success  in  our  target  markets
including with respect to future revenues generated by Ocaliva.

Delays or difficulties in the commencement, enrollment and completion of our clinical trials and studies could increase
our product development costs and delay, limit or prevent us from obtaining regulatory approval for OCA and our other
product candidates.

Delays or difficulties in the commencement, enrollment and completion of our clinical trials and studies could increase
our product development costs and limit or prevent us from obtaining or maintaining regulatory approval for OCA and our
other product candidates. We are currently conducting a number of clinical trials, including our Phase 4 COBALT clinical
outcomes confirmatory trial of Ocaliva for PBC, our Phase 3 REGENERATE trial of OCA in patients with liver fibrosis
due to NASH through clinical outcomes in order to confirm clinical benefit and our Phase 3 REVERSE trial of OCA for
NASH  patients  with  compensated  cirrhosis.  We  are  also  conducting  our  CARE  trial  of  OCA  in  pediatric  patients  with
biliary atresia as a part of an EMA-approved PIP supporting the conditional approval of Ocaliva for PBC. The results from
these  clinical  trials  and  our  other  clinical  trials  and  studies  may  not  be  available  when  we  anticipate  and  we  may  be
required to conduct additional clinical trials or studies not currently planned in order for our product candidates, including
OCA for PBC and NASH, to be approved or to maintain approvals in the U.S., Europe or the other jurisdictions in which
our products are approved. In addition, our clinical programs are subject to a number of risks and uncertainties, such as the
results of other trials, patient enrollment, safety issues or regulatory interactions that could result in a change of trial design
or timing. For example, we recently paused enrollment in our Phase 4 COBALT confirmatory outcomes trial evaluating
Ocaliva for PBC and in our Phase 4 clinical trial of Ocaliva in patients with PBC who have moderate to severe hepatic
impairment (Child-Pugh B and C) known as the 401 trial pending the results of discussions with the FDA and the EMA
regarding proposals with respect to such trials. Any delays or difficulties completing such trials as a result of the pause in
enrollment could increase our product development costs and limit or prevent us from obtaining or maintaining regulatory
approval. Consequently, we do not know whether our current or future clinical trials or studies of OCA or our other product
candidates will be completed on schedule, if at all.

The  commencement,  enrollment  and  completion  of  our  clinical  trials  and  studies  may  be  delayed,  suspended  or

otherwise adversely affected for a variety of reasons, including:

● our inability to obtain sufficient funds to complete or continue our clinical trials;

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● our  inability  to  reach  agreements  on  acceptable  terms  with  prospective  contract  research  organizations
(“CROs”)  and  trial  sites,  the  terms  of  which  may  be  subject  to  extensive  negotiation  and  may  vary
significantly among our various CROs and trial sites;

● clinical holds, other regulatory objections to our commencing or continuing a clinical trial or our inability to

obtain regulatory approval to commence clinical trials in countries that require such approvals;

● our discussions with the FDA, EMA or other regulatory authorities prior to, or following, the initiation of our
clinical  trials,  regarding,  among  other  matters,  the  scope  or  design  of  our  clinical  trials,  including  trial
endpoints, protocols and statistical analysis plans, and any modifications thereto;

● our  inability  to  identify  and  maintain  a  sufficient  number  of  trial  sites,  many  of  which  may  already  be
engaged in other clinical trial programs, including some that may be for the same indications targeted by our
product candidates;

● any delay in receiving results from, or failure to achieve the necessary results in, our clinical trials;

● our inability to obtain approval from institutional review boards or independent ethics committees to conduct

our clinical trials at their respective sites;

● any data monitoring committee recommendation that our clinical trials be modified, suspended or terminated

due to safety, lack of efficacy or other reasons;

● severe or unexpected drug-related adverse events experienced by patients or any determination that a clinical

trial presents unacceptable health risks;

● any  breach  of  the  terms  of  any  relevant  agreement  by  us,  our  current  or  future  collaborators  that  have
responsibility  for  the  clinical  development  of  any  of  our  product  candidates  or  investigators  conducting
clinical trials on our product candidates;

● our  inability  to  timely  manufacture,  or  obtain  from  our  contract  manufacturers,  sufficient  quantities  of  our

product candidate required for our clinical trials; and

● any difficulty recruiting, enrolling or retaining patients in our clinical trials based on, among other factors,
the  enrollment  criteria  for  our  clinical  trials,  the  rarity  of  the  disease,  the  characteristics  of  the  population
being studied, the risks of the procedures that may be required as part of the clinical trials, such as a liver
biopsy,  the  availability  of  our  products  to  patients  generally  following  the  approval  of  such  products  or
competition  from  other  clinical  trial  programs  recruiting  patients  for  the  same  indications  as  our  product
candidates.

For  example,  our  Phase  3  REGENERATE  trial  is  a  large  and  complicated  clinical  trial  in  a  disease  without  any
approved therapies and involves serial liver biopsies over many years. While we announced topline results from the 18-
month analysis of our pivotal Phase 3 REGENERATE trial in February 2019, the study is currently planned to continue
through clinical outcomes in order to confirm clinical benefit and there can be no assurance that we will retain a sufficient
number of patients in the full study cohort or complete the clinical outcomes trial in accordance with the study protocol or
on a timely basis, if at all. Similarly, our COBALT clinical outcomes confirmatory trial for PBC includes subjects across
the  spectrum  of  PBC  disease,  including  early  and  advanced  PBC.  Enrolling  and  retaining  patients  in  such  trials  is
challenging and there can be no assurance that we will complete the clinical outcomes trial in accordance with the study
protocol or on a timely basis, if at all. As we engage in other large and complicated trials and trials in advanced disease
populations,  we  may  experience  a  number  of  challenges  that  may  negatively  affect  or  delay  our  plans  and  development
programs.

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We have in the past experienced difficulties enrolling and retaining patients enrolled in our clinical trials. Difficulties
in  enrolling  and  retaining  patients,  including  due  to  COVID-19,  may  delay  our  clinical  trials  or  result  in  negative  or
inconclusive  outcomes,  and  we  or  our  collaborators  may  decide,  or  regulatory  authorities  may  require  us,  to  conduct
additional  clinical  trials  or  additional  analyses  of  existing  clinical  trials.  Any  delay  or  compromises  with  respect  to  the
validity  of  our  clinical  trials  may  have  a  material  adverse  effect  on  our  business  or  decrease  our  competitive  position
relative to other biotechnology or pharmaceutical companies with whom we compete.

In addition, if we or any of our collaborators are required to conduct additional preclinical or clinical studies or other
development work on our product candidates beyond that contemplated, our ability to obtain regulatory approval of these
product candidates and generate revenue from their sales would be similarly harmed.

COVID-19 could materially and adversely affect our clinical trials.

COVID-19 is a global pandemic, affecting the U.S., Europe, and other countries in which we are engaged in, or plan to
engage in, clinical development activities. We continue to closely monitor the COVID-19 pandemic and, together with our
contract research organizations, study sites and other partners, have taken measures intended to minimize disruptions and
protect and retain patients enrolled in our clinical trials, including, where appropriate, the use of telemedicine, home care
visits,  direct  delivery  of  investigational  product  and  other  measures.  Notwithstanding  our  efforts,  some  of  the  sites
participating in our clinical trials have been affected by site closings or reduced capacity, particularly in regions that are
experiencing  heightened  impact  from  COVID-19.  While  we  continue  to  monitor  the  situation  closely,  if  there  was  a
meaningful  negative  impact  on  the  data  capture  or  data  quality  of  any  of  our  clinical  trials,  such  trials  may  not  be
successful or we could be required to repeat, extend the duration of, increase the size of, or otherwise modify such trials,
which could prevent or significantly delay the potential commercialization of our product candidates and require greater
expenditures. We cannot at this time predict with certainty the scope of the impact of COVID-19 on our ability to execute
our  clinical  trials.  The  extent  to  which  COVID-19  may  impact  our  clinical  trials  will  depend  on  future  developments,
which are highly uncertain, such as the continued geographic spread of the disease, the duration of the pandemic, public
health restrictions on travel and in-person interactions, business closures and disruptions, and the effectiveness of actions
taken to contain and treat the disease. As a result, our clinical trials may not be successful or we may experience issues due
to COVID-19 that could severely impact our clinical trials, including:

● delays,  interruptions  or  difficulties  in  the  enrollment,  scheduling  and  retention  of  patients  in  our  clinical

trials;

● delays,  interruptions  or  difficulties  in  the  conduct  of  key  clinical  trial  activities,  such  as  clinical  trial  site

monitoring and inspection readiness activities;

● trial  conduct  issues,  including  protocol  deviations  (e.g.,  failure  to  timely  collect  liver  biopsies  or  other

required laboratory data), data capture issues and data quality issues;

● delays  or  interruptions  in  the  supply  or  administration  of  investigational  product  to  patients  in  our  clinical

trials;

● delays or interruptions in the supply of necessary equipment or materials to clinical sites;

● delays  or  difficulties  obtaining  approvals  from  regulatory  authorities,  institutional  review  boards  or  ethics
committees  of  clinical  trial  protocols  and  related  clinical  documentation  (or  amendments  and  addendums
thereto);

● delays, interruptions or difficulties in clinical site initiations, including in connection with the recruitment of

clinical site investigators and clinical site staff;

● the  redeployment  of  healthcare  resources,  including  clinical  site  investigators  and  clinical  site  staff

supporting the conduct of our clinical trials, to assist in the treatment of COVID-19 patients;

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● the  diversion  of  human  capital,  including  employees,  independent  contractors,  vendors  and  other  third
parties, otherwise focused on the conduct of our clinical trials due to sickness, safety concerns or government
or employer imposed travel or working restrictions;

● new federal, state and local government regulations or guidance that require us to change the way we conduct
our clinical trials, require the interruption or termination of our clinical trials or that result in significant and
unexpected new costs;

● delays or difficulties in interactions with regulatory authorities, institutional review boards, ethics committees
and  key  consultants  and  vendors  due  to  layoffs,  temporary  leaves,  terminations  or  other  actions  limiting
available employee resources; and

● the refusal of regulatory authorities to accept clinical trial data from clinical trials that have been negatively

affected by COVID-19.

Any such delay, interruption or issue could materially and adversely affect our business, financial condition and results

of operations.

Failure can occur at any stage of clinical development. The results of earlier clinical trials are not necessarily predictive
of  future  results  and  any  product  candidate  we  or  our  collaborators  advance  through  clinical  trials,  including  OCA,
may not have favorable results in later clinical trials or receive or maintain regulatory approval.

Clinical failure can occur at any stage of clinical development. Clinical trials may produce negative or inconclusive
results,  and  we  or  our  collaborators  may  decide,  or  regulators  may  require  us,  to  conduct  additional  clinical  trials  or
preclinical  studies.  In  addition,  data  obtained  from  trials  and  studies  are  susceptible  to  varying  interpretations,  and
regulators may not interpret our data as favorably as we do, which may delay, limit or prevent regulatory approval. Success
in preclinical studies and early clinical trials does not ensure that subsequent clinical trials will generate the same or similar
results or otherwise provide adequate data to demonstrate the efficacy and safety of our product candidates. A number of
companies  in  the  pharmaceutical  industry,  including  those  with  greater  resources  and  experience  than  us,  have  suffered
significant setbacks in Phase 3 clinical trials and at other stages of clinical development, even after seeing promising results
in earlier clinical trials.

In addition, the design of clinical trials, including trial endpoints, protocols and statistical analysis plans, can determine
whether such trials will support product approvals, and flaws in the design of such trials may not become apparent until
such  trials  are  well-advanced.  We  may  be  unable  to  design  and  execute  clinical  trials  to  support  regulatory  approval.
Further, clinical trials of product candidates often reveal that it is not practical or feasible to continue development efforts.
If OCA or our other product candidates are found to be unsafe or lack sufficient efficacy for any indication, we will not be
able to obtain or maintain regulatory approval for them, and our prospects and business may be materially and adversely
affected.

There may be significant variability in the safety and/or efficacy results we see in different trials studying OCA or our
other product candidates due to numerous factors, including differences in the underlying disease being studied, changes or
differences  in  trial  protocols  or  statistical  analysis  plans,  differences  in  the  composition  of  the  patient  populations  or
clinical trial sites, differences in adherence to the dosing regimen and other aspects of the trial protocols and differences in
the rate of dropouts among clinical trial participants. We do not know whether any Phase 2, Phase 3 or other clinical trials
we or any of our collaborators may conduct on our product candidates will demonstrate consistent or adequate efficacy and
safety or result in the approval of our product candidates by regulatory authorities. If we are unable to bring any of our
current  or  future  product  candidates  to  market,  acquire  any  previously  approved  products  or  maintain  approval  for  our
approved products, our ability to create long-term stockholder value will be limited.

Although  Ocaliva  for  PBC  has  received  accelerated  approval  in  the  United  States  and  conditional  approval  in  the
European Union, its full approval depends on the timely completion and results of post-marketing clinical trials, including
our Phase 4 COBALT trial. We cannot assure you that these trials will be timely completed or that the results of such trials

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will support the full approval of Ocaliva in the United States, European Union or our other target markets where Ocaliva
has not received full approval.

In December 2014, we received comprehensive datasets from the Phase 2b FLINT trial for the treatment of NASH,
which met its primary endpoint with statistical significance. In October 2015, we announced that the Phase 2 dose ranging
trial  of  OCA  in  200  adult  NASH  patients  in  Japan  conducted  by  our  former  collaborator,  Sumitomo  Dainippon,  did  not
meet  its  primary  endpoint  with  statistical  significance.  In  the  Sumitomo  Dainippon  trial,  there  was  a  dose  dependent,
although not statistically significant, increase in the percentage of OCA-treated patients compared to placebo who achieved
the primary endpoint (p = 0.053). In addition, no difference was seen in fibrosis improvement in the OCA groups compared
to placebo. The Sumitomo Dainippon Phase 2 trial involved different doses of OCA being administered to the trial subjects
than  those  utilized  in  the  Phase  2b  FLINT  trial.  Furthermore,  the  baseline  characteristics  between  the  patients  in  the
Japanese Phase 2 dose ranging trial conducted by Sumitomo Dainippon were distinct in a number of ways from those of
the Western patients included in the Phase 2b FLINT trial.

In February 2019, we announced topline results from the 18-month analysis of our pivotal Phase 3 REGENERATE
trial  in  patients  with  liver  fibrosis  due  to  NASH.  In  the  primary  efficacy  analysis,  once-daily  OCA  25  mg  met,  with
statistical significance, the primary endpoint agreed with the FDA of fibrosis improvement by at least one stage with no
worsening of NASH (defined as no worsening of hepatocellular ballooning, no worsening of lobular inflammation and no
worsening  of  steatosis)  at  the  planned  18-month  analysis.  Although  a  numerically  greater  proportion  of  patients  in  both
OCA treatment groups compared to placebo achieved the primary endpoint of NASH resolution with no worsening of liver
fibrosis in the primary efficacy analysis, this result did not reach statistical significance. As agreed with the FDA, in order
for the primary objective to be met, the study was required to achieve one of the two primary endpoints. Notwithstanding
the results of the REGENERATE 18-month analysis, the recent CRL issued by the FDA indicated that, based on the data
the FDA had reviewed, the FDA had determined that the predicted benefit of OCA based on a surrogate histopathologic
endpoint remains uncertain and does not sufficiently outweigh the potential risks to support accelerated approval for the
treatment  of  patients  with  liver  fibrosis  due  to  NASH.  The  FDA  recommended  that  we  submit  additional  post-interim
analysis efficacy and safety data from the ongoing REGENERATE study in support of potential accelerated approval and
that the long-term outcomes phase of the study should continue. Although we are in discussions with the FDA with respect
to the potential resubmission of our NDA seeking accelerated approval of OCA for the treatment of liver fibrosis due to
NASH, there is no assurance that we will be successful or that OCA will be approved for liver fibrosis due to NASH on an
accelerated basis, or at all. While OCA received breakthrough therapy designation from the FDA in January 2015 for the
treatment of NASH patients with liver fibrosis and we filed a NDA in the United States and a MAA in Europe for approval
of OCA for liver fibrosis due to NASH based on the results from the 18-month analysis of our Phase 3 REGENERATE
trial in patients with liver fibrosis due to NASH, we do not know if one pivotal clinical trial will be sufficient for marketing
approval or if regulatory authorities in the United States, Europe or our other target markets will approve OCA for liver
fibrosis due to NASH on an accelerated or conditional basis, or at all. Additionally, interim analysis results at 18 months
were  based  on  surrogate  endpoints  and  the  impact  on  clinical  outcomes  has  not  been  confirmed.  Our  Phase  3
REGENERATE trial remains ongoing through clinical outcomes for verification and description of clinical benefit of OCA
for liver fibrosis due to NASH.

Our  product  candidates  may  have  undesirable  side  effects  which  may  delay  or  prevent  marketing  approval,  or,  if
approval is received, require that our products be taken off the market or include new or additional safety warnings.
Any  such  events  may  limit  our  existing  and  future  product  sales  and  materially  and  adversely  affect  our  business,
financial condition and results of operations.

OCA  has  been  shown  to  be  a  potent  FXR  agonist.  With  the  exception  of  the  endogenous  human  bile  acid
chenodeoxycholic  acid  and  cholic  acid,  there  are  no  approved  FXR  agonists  and  the  adverse  effects  from  long-term
exposure  to  this  drug  class  are  unknown.  Unforeseen  side  effects  from  any  of  our  product  candidates,  including  OCA,
could  arise  either  during  clinical  development  or,  if  approved,  after  the  approved  product  has  been  marketed.  Serious
adverse events, including deaths, in patients taking OCA have occurred in clinical trials and in the post-marketing setting,
and  we  cannot  assure  you  that  additional  serious  adverse  events  in  patients  taking  OCA  in  clinical  trials  or  in  the  post-
marketing setting will not occur.

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The most common side effects observed in clinical trials of OCA for PBC were pruritus, fatigue, headaches, nausea,
constipation  and  diarrhea.  In  our  Phase  3  POISE  trial,  pruritus,  generally  mild  to  moderate,  was  the  most  frequently
reported adverse event associated with OCA treatment for PBC and was observed in 38% of patients on placebo, 70% of
patients  in  the  OCA  10  mg  group  and  56%  of  patients  in  the  OCA  titration  group  (5  mg  to  10  mg).  Eight  patients
discontinued due to pruritus, of whom none were in the placebo group, seven (10%) were in the OCA 10 mg group and one
(1%) was in the OCA titration group. Pruritus also has been observed in other clinical trials of OCA. Decreases in high
density lipoprotein HDL cholesterol were also observed during treatment in our Phase 3 POISE trial. In our Phase 2 trials
for OCA for PBC, a dose-response relationship was observed in the occurrence of liver-related adverse reactions, including
jaundice, ascites and primary biliary cholangitis flare with dosages of OCA of 10 mg once daily to 50 mg once daily (up to
5-times the highest recommended dosage), as early as one month after starting treatment with OCA. The European label
for Ocaliva also notes that elevations in alanine amino transferase and aspartate aminotransferase were observed in patients
treated with OCA.

In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended  weekly  dose  in  such  patients.  As  a  result,  in  September  2017,  we  issued  a  Dear  Health  Care  Provider
(“DHCP”)  letter,  and  the  FDA  also  subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended
label dosing. Both communications remind healthcare providers of the importance of the recommended reduced dosing of
Ocaliva in PBC patients with moderate or severe hepatic impairment, while reiterating the importance of monitoring PBC
patients  for  progression  of  their  disease  and  the  occurrence  of  liver-related  adverse  reactions.  In  addition  to  the  DHCP
letter,  we  took  actions  to  enhance  education  about  appropriate  use  of  Ocaliva.  These  initiatives  included:  reeducating
physicians  on  the  label,  with  a  focus  on  ensuring  appropriate  dosing  for  patients  with  moderate  or  severe  hepatic
impairment; enhancing monitoring of patients for liver-related adverse reactions; and adjudicating reported cases of serious
liver injury, including in patients with no or mild hepatic impairment. In February 2018, we announced that the Ocaliva
label in the United States had been updated by the FDA to include a boxed warning and a dosing table that reinforced the
then-existing dosing schedule for patients with Child-Pugh Class B or C or decompensated cirrhosis. In addition, the FDA
issued an updated drug safety communication to accompany the revised label. We remain focused on the safety of all of the
patients  using  Ocaliva  within  and  outside  of  our  ongoing  clinical  studies  and  have  engaged  with  relevant  regulatory
authorities  to  ensure  that  the  Ocaliva  label  sufficiently  reinforces  the  importance  of  appropriate  dosing  in  patients  with
advanced cirrhosis.

The FDA has notified us that, in the course of its routine safety surveillance, in May 2020 the FDA began to evaluate a
newly identified safety signal, or NISS, regarding liver disorder for Ocaliva which the FDA classified as a potential risk.
The  FDA  has  informed  us  that  its  review  of  the  NISS  is  focused  on  a  subset  of  the  cirrhotic,  or  more  advanced,  PBC
patients who have taken Ocaliva. As part of our routine pharmacovigilance efforts, we worked with the FDA to reconcile
our internal safety database with the FDA Adverse Event Reporting System database and we completed a comprehensive
assessment of all available data, including data from our completed clinical trials, blinded reviews of ongoing clinical trial
data,  unblinded  reviews  of  certain  ongoing  clinical  trial  data  by  the  DMC,  post-marketing  data  and  natural  history  data,
which we submitted to the FDA and had a meeting earlier in 2021 to discuss. We are working with the FDA to align on
changes to the Ocaliva label regarding patients with the most advanced stages of PBC. Based on our communications with
the FDA, this update will come in the form of a safety labeling change. These communications are ongoing and any safety
concerns  associated  with  Ocaliva,  perceived  or  real,  may  adversely  affect  the  successful  development  and
commercialization of our product candidates and approved products, including Ocaliva, and materially and adversely affect
our business including future revenue generated by Ocaliva.

Ocaliva is contraindicated for PBC patients with complete biliary obstruction in the United States and the European
Union. For PBC patients with HDL reductions and no response to Ocaliva after one year at the maximum tolerated dose,
the U.S. label asks prescribing physicians to weigh the risks against the benefits of continuing treatment.

In the 18-month analysis of our pivotal Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH, the
safety population included 1,968 randomized patients who received at least one dose of investigational product (OCA or
placebo)  with  exposures  up  to  37  months.  Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most
common were consistent with the known profile of OCA. The frequency of serious adverse events was similar across

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treatment groups (11% in placebo, 11% in OCA 10 mg and 14% in OCA 25 mg), and no serious adverse event occurred in
> 1% of patients in any treatment group. There were 3 deaths in the study (2 in placebo: bone cancer and cardiac arrest and
1 in OCA 25 mg: glioblastoma) and none were considered related to treatment. The most common adverse event reported
was dose-related pruritus (19% in placebo, 28% in OCA 10 mg and 51% in OCA 25 mg). The incidence of pruritus across
all  three  treatment  groups  was  highest  in  the  first  three  months  and  decreased  thereafter.  The  large  majority  of  pruritus
events were mild to moderate, with severe pruritus occurring in a small number of patients (< 1% in placebo, < 1% in OCA
10 mg and 5% in OCA 25 mg). A higher incidence of pruritus-associated treatment discontinuation was observed for OCA
25  mg  (<  1%  in  placebo,  <  1%  in  OCA  10  mg  and  9%  in  OCA  25  mg).  According  to  the  clinical  study  protocol,
investigator  assessed  severe  pruritus  mandated  treatment  discontinuation.  Consistent  with  observations  from  previous
NASH studies, OCA treatment was associated with an increase in low density lipoprotein (“LDL”) cholesterol, with a peak
increase of 22.6 mg/dL at 4 weeks and subsequently reversing and approaching baseline at month 18 (4.0 mg/dL increase
from  baseline).  Triglycerides  rapidly  and  continually  decreased  in  the  OCA  treatment  groups  through  month  18.  There
were few and varied serious cardiovascular events and incidence was balanced across the three treatment groups (2% in
placebo, 1% in OCA 10 mg and 2% in OCA 25 mg). In patients with type 2 diabetes, OCA treatment was associated with
an early transient increase in fasting glucose and hemoglobin A1c with return to levels similar to placebo by month 6. No
clinically meaningful changes were noted in non-diabetic patients.

With  respect  to  hepatobiliary  events,  more  patients  (3%)  on  OCA  25  mg  experienced  gallstones  or  cholecystitis
compared to < 1% on placebo and 1% on OCA 10 mg. While hepatic serious adverse events were rare (< 1% incidence in
each of the three treatment groups), more occurred in the OCA 25 mg group with no pattern attributable to OCA.

In  the  Phase  2b  FLINT  trial,  pruritus  occurred  more  frequently  in  the  OCA  treatment  group  than  in  the  placebo
treatment group (23% vs. 6%, p < 0.0001) and at a higher grade (predominately moderate pruritus). OCA treatment was
also  associated  with  changes  in  serum  lipid  levels,  including  increases  in  total  cholesterol  and  LDL  cholesterol  and  a
decrease  in  HDL  cholesterol,  that  were  observed  within  12  weeks  of  initiating  treatment,  peaked  and  then  decreased  in
magnitude while on treatment, and reversed further during the 24-week post-treatment period. These changes in cholesterol
levels,  along  with  the  achievement  of  pre-defined  efficacy  criteria,  played  a  role  in  the  decision  of  the  FLINT  data  and
safety monitoring board to terminate the treatment phase of the Phase 2b FLINT trial, and the publication of the FLINT
results noted the need for further study of these changes. There were two patient deaths in the Phase 2b FLINT trial, and
neither death was considered related to OCA treatment.

Furthermore, the Phase 2 dose ranging trial of OCA in 200 adult NASH patients in Japan conducted by our former
collaborator, Sumitomo Dainippon, did not meet statistical significance for the primary endpoint. The primary endpoint in
the Sumitomo Dainippon trial was histologic improvement defined as at least a two-point improvement in the nonalcoholic
fatty  liver  disease  activity  score  with  no  worsening  of  fibrosis.  In  this  trial,  there  was  a  dose  dependent,  although  not
statistically significant, increase in the percentage of OCA-treated patients compared to placebo who achieved the primary
endpoint (p = 0.053). In addition, no difference was seen in fibrosis improvement in the OCA groups compared to placebo.

  In  December  2015,  we  initiated  a  Phase  2  clinical  trial,  known  as  the  CONTROL  trial,  to  characterize  the  lipid
metabolic  effects  of  OCA  and  cholesterol  management  effects  of  concomitant  statin  administration  in  NASH  patients.
CONTROL enrolled 80 NASH patients who were naïve to statin therapy or had undergone a statin washout period. The
study included a 16-week double-blind phase followed by an optional long-term safety extension (“LTSE”) phase of the
trial.  OCA  treatment  in  the  absence  of  statin  therapy  over  the  first  four  weeks  resulted  in  an  increase  in  LDL  across  all
OCA treatment groups, while the placebo group was relatively unchanged. Treatment with atorvastatin beginning at week
four  and  continuing  through  week  16  reversed  OCA-related  increases  in  LDL  to  below  baseline  levels  in  all  OCA
treatment groups. Dose-dependent pruritus was the most common adverse event in patients treated with OCA, occurring in
5% of patients on placebo, 5% of patients in the OCA 5 mg group, 10% of patients in the OCA 10 mg group and 55% of
patients in the OCA 25 mg group. All adverse events were mild to moderate and two patients discontinued treatment in the
OCA 25 mg group due to pruritus. Over 95% of the patients completing the double-blind phase of CONTROL enrolled in
the LTSE phase of the trial.

During the LTSE phase of CONTROL, there was one patient death. This patient was a 64 year-old male with a history
of NASH associated liver cirrhosis, morbid obesity (BMI >40) and type 2 diabetes. At baseline, this patient had blood tests
consistent with impaired liver function (e.g., low LDL and low platelets). The patient was randomized to placebo for the

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double-blind phase of the study. Early in the double-blind phase, the patient had serum biochemistry changes consistent
with  worsening  hepatic  impairment  (e.g.,  albumin  decline  and  bilirubin  was  increasing).  Atorvastatin  was  started  per
protocol  and  then  stopped  early  due  to  the  patient’s  persistently  low  LDL  levels.  The  patient  later  enrolled  in  the  LTSE
phase  and  began  receiving  OCA  25  mg  treatment.  Over  the  following  four  months,  the  patient’s  serum  biochemistry
remained  consistent  with  ongoing  hepatic  impairment.  Approximately  five  months  after  starting  the  LTSE  phase,  the
patient  developed  severe  protracted  diarrhea,  which  resulted  in  weight  loss  of  30  pounds  over  the  ensuing  one-month
period.  Both  an  infectious  cause  and  possible  inflammatory  bowel  disease  were  suspected,  and  the  patient  subsequently
was  started  on  broad  spectrum  antibiotics  and  steroid  therapy.  Due  to  the  diarrhea,  the  principal  investigator  stopped
treatment with OCA and discontinued the patient from the study. Concurrently, the patient reported jaundice and was found
to  have  significantly  elevated  serum  bilirubin  and  ALP,  while  other  liver  enzymes  remained  relatively  stable.  Over  the
ensuing  two-week  period,  various  diagnostic  tests  and  procedures  were  performed  (e.g.,  magnetic  resonance
cholangiopancreatography  to  investigate  possible  gallstone  bile  duct  obstruction)  and  the  patient  continued  receiving  a
number of other medications, including the ongoing course of steroid therapy. During this time, the patient continued to
deteriorate and was hospitalized with acute renal and liver failure, complicated by severe metabolic acidosis. The patient
rapidly  progressed  to  multi-organ  system  failure,  sepsis  and  death.  The  principal  investigator  determined  that  the  events
leading to the patient’s death were unlikely related to OCA. Despite the numerous confounding factors in this case, given
the contemporaneous administration of OCA during the patient’s ongoing deterioration, we determined that it could not be
ruled out that these events were possibly related to treatment. Subsequent to our determination, the independent data safety
monitoring  committee  separately  evaluated  the  case  and  determined  that  the  events  leading  to  the  patient’s  death  were
unlikely related to OCA.

Additional or unforeseen side effects relating to OCA or any of our other product candidates could arise either during
clinical development or, if approved, after the approved product has been marketed. With the approval of Ocaliva for PBC
in the United States, Europe and certain of our other target markets, OCA is currently used in an environment that is less
rigorously  controlled  than  in  clinical  studies.  If  new  side  effects  are  found,  if  known  side  effects  are  shown  to  be  more
severe than previously observed or if OCA is shown to have other unexpected characteristics, we may need to abandon our
development of OCA for PBC, NASH and other potential indications. Furthermore, our commercial sales of Ocaliva for
PBC may be materially and adversely affected.

The  range  and  potential  severity  of  possible  side  effects  from  systemic  therapies  is  significant.  The  results  of  our
current or future clinical trials may show that our product candidates, including OCA, cause undesirable or unacceptable
side effects, which could interrupt, delay or halt clinical trials, result in a delay of, or failure to obtain, marketing approval
from the FDA and other regulatory authorities, result in marketing approval from the FDA and other regulatory authorities
with restrictive label warnings or result in the withdrawal of previously granted marketing approvals.

In  addition,  our  product  candidates  are  being  developed  as  potential  treatments  for  severe,  life  threatening  diseases
and,  as  a  result,  our  trials  will  necessarily  be  conducted  in  patient  populations  that  are  more  prone  than  the  general
population to exhibit certain disease states or adverse events. For example, our Phase 3 REVERSE trial in NASH patients
with  compensated  cirrhosis  has  expanded  our  NASH  development  program  into  a  more  advanced  NASH  patient
population  and  accordingly  imposes  certain  eligibility  requirements  for  uptitration,  as  well  as  certain  monitoring
requirements  thereafter.  Ocaliva  is  prescribed  in  patients  suffering  from  various  stages  of  PBC,  which  can  be  life
threatening, and patients may suffer from other concomitant illnesses that may increase the likelihood of certain adverse
events. It may be difficult to discern whether certain events or symptoms observed during our clinical trials or by patients
using our approved products are related to our product candidates or approved products or some other factor. As a result,
we and our development programs may be negatively affected even if such events or symptoms are ultimately determined
to be unlikely related to our product candidates or approved products. We cannot assure you that additional or more severe
adverse  side  effects  related  to  OCA  or  our  other  product  candidates  will  not  be  observed  in  our  clinical  trials  or  in  the
commercial  setting.  If  observed,  such  adverse  side  effects  could  delay  or  preclude  regulatory  approval  of  OCA,  limit
commercial use or result in the withdrawal of previously granted marketing approvals.

If we or others identify undesirable or unacceptable side effects caused by our product candidates or products:

● we may be required to modify, suspend or terminate our clinical trials;

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● we  may  be  required  to  modify  or  include  additional  dosage  and  administration  instructions,  warnings  and
precautions,  contraindications,  boxed  warnings,  limitations,  restrictions  or  other  statements  in  the  product
label for our approved products, or issue field alerts to physicians and pharmacies or implement other risk
mitigation programs;

● we may be required to conduct costly additional clinical trials;

● we may be subject to limitations on how we may promote our approved products;

● sales of our approved products may decrease significantly;

● regulatory authorities may require us to take our approved products off the market;

● we  may  be  subject  to  regulatory  investigations,  government  enforcement  actions,  litigation  or  product

liability claims; and

● our products may become less competitive or our reputation may suffer.

Breakthrough therapy designation for OCA may not lead to faster development or regulatory processes or increase the
likelihood that the FDA will approve OCA for the treatment of NASH patients with fibrosis.

If  a  drug  is  intended  for  the  treatment  of  a  serious  or  life-threatening  condition  and  preliminary  clinical  evidence
indicates  that  the  drug  may  demonstrate  substantial  improvement  over  existing  therapies  on  one  or  more  clinically
significant endpoints, such as substantial treatment effects observed early in clinical development, the FDA may grant a
breakthrough therapy designation. Breakthrough therapy designation is intended to facilitate the development, and expedite
the review, of such drugs, but the breakthrough therapy designation does not assure marketing approval by the FDA.

In January 2015, we received breakthrough therapy designation for OCA for the treatment of NASH patients with liver
fibrosis.  However,  there  is  no  guarantee  that  the  receipt  of  breakthrough  therapy  designation  will  result  in  a  faster
development process, review or approval of OCA for liver fibrosis due to NASH or increase the likelihood that OCA will
be granted marketing approval for NASH patients with liver fibrosis. Notwithstanding our receipt of breakthrough therapy
designation, in June 2020 we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to
NASH.  Although  we  are  in  discussions  with  the  FDA  with  respect  to  the  potential  resubmission  of  our  NDA  seeking
accelerated approval of OCA for the treatment of liver fibrosis due to NASH, there is no assurance that the outcome of
these discussions will lead to resolution of the issues identified in the CRL or that if we resubmit our NDA that it will be
approved. Similarly, any future breakthrough therapy designation relating to any other potential indication of OCA or our
other  product  candidates  will  neither  guarantee  a  faster  development  process,  review  or  approval  nor  improve  the
likelihood of the grant of marketing approval by the FDA compared to conventional FDA procedures. In addition, the FDA
may withdraw any breakthrough therapy designation at any time. While we may seek breakthrough therapy designation for
one or more of our product candidates in the future, we can give no assurance that the FDA will grant such status.

We may not be able to obtain or, if approved, maintain orphan drug exclusivity for our approved products or product
candidates, which could cause our revenues to suffer.

Regulatory  authorities  in  some  jurisdictions,  including  the  United  States  and  Europe,  may  designate  drugs  and
biologics for relatively small patient populations as orphan drugs. Under the Orphan Drug Act, the FDA may designate a
product as an orphan drug if it is a drug or biologic intended to treat a rare disease or condition, which is generally defined
as  a  patient  population  of  fewer  than  200,000  individuals  annually  in  the  United  States.  OCA  has  received  orphan  drug
designation in the United States and the European Union for the treatment of PBC and PSC.

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Generally,  if  a  product  with  an  orphan  drug  designation  subsequently  receives  the  first  marketing  approval  for  the
indication for which it has such designation, the product is entitled to a period of marketing exclusivity, which precludes
the  FDA  or  the  EMA  from  approving  another  marketing  application  for  the  same  product  during  the  exclusivity  period.
The applicable exclusivity period is seven years in the United States and ten years in Europe. Orphan drug exclusivity may
be lost if the FDA or EMA determines that the request for designation was materially defective or if the manufacturer is
unable  to  assure  a  sufficient  quantity  of  the  product  to  meet  the  needs  of  patients  with  the  rare  disease  or  condition.  In
addition, the European exclusivity period can be reduced to six years if, at the end of the fifth year, it is established that the
product no longer meets the criteria for orphan drug designation because, for example, the product is sufficiently profitable
not to justify maintenance of market exclusivity.

Any failure to maintain orphan drug status may subject us to mandatory price discounts in Europe and result in the loss
of other benefits, such as tax exemptions for sales. As such, the loss of orphan drug status may have a negative effect on
our ability to successfully commercialize our products, earn revenues and achieve profitability.

Even if we obtain orphan drug exclusivity for a product, that exclusivity may not effectively protect the product from
competition because different products can be approved for the same condition. Even after an orphan drug is approved, the
FDA or EMA may subsequently approve another product for the same condition if the FDA or EMA concludes that the
later  product  is  clinically  superior  (i.e.,  it  is  shown  to  be  safer,  more  effective  or  makes  a  major  contribution  to  patient
care). Any inability to secure or maintain orphan drug status or the exclusivity benefits of this status could have a material
adverse impact on our ability to develop and commercialize our product candidates and approved products.

We  rely  entirely  on  third  parties  for  the  manufacture  of  our  product  requirements  for  our  preclinical  studies  and
clinical trials, as well as our commercial supply of Ocaliva and, if approved, OCA for liver fibrosis due to NASH and
our  other  product  candidates,  and  also  depend  on  third-party  vendors  and  CROs  for  certain  of  our  clinical  trial  and
product development activities. Our business could be harmed if our third-party manufacturers fail to provide us with
sufficient quantities of drug product, or fail to do so at acceptable quality levels or prices, or if our third-party vendors
or  CROs  assisting  us  with  our  clinical  trials  and  product  development  activities  fail  to  comply  with  their  contractual
commitments  or  applicable  regulatory  obligations  or  if  we  lose  our  relationships  with  our  third-party  vendors  and
CROs.

We do not manufacture the pharmaceutical products that we sell or the product candidates that we are developing. We
rely  on  third-party  contract  manufacturers  for  all  of  our  required  raw  materials,  active  pharmaceutical  ingredient  and
finished product for our commercial sales and for our existing and anticipated clinical trials and preclinical studies. Any
inability by our contract manufacturers to continue to provide services to us for any reason, including due to COVID-19
and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel  and  in-person  interactions,  business
closures  and  disruptions  and  other  public  health  safety  measures,  could  disrupt  the  supply  chain  for  our  pharmaceutical
products  and  product  candidates  and  materially  and  adversely  affect  our  commercialization  efforts  and  clinical
development  program,  and  we  may  be  unable  to  identify,  qualify  and  engage  replacement  suppliers  on  terms  that  are
favorable to us on a timely basis, if at all. The extent to which COVID-19 impacts the operations of our third-party contract
manufactures  will  depend  on  future  developments,  which  are  highly  uncertain  and  cannot  be  predicted  with  confidence,
including  the  geographic  spread  of  the  disease,  the  duration  of  the  outbreak,  public  health  safety  measures  and  the
effectiveness of the actions taken to contain and treat the disease.

We  rely  on  PharmaZell  GmbH  and  other  suppliers  for  the  manufacture  and  commercial  supply  of  API  for  use  in
Ocaliva  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH.  We  are  currently  dependent  upon  a  limited  number  of
suppliers, with whom we have contractual arrangements, although we are working on developing further sources of supply.
While we have procured supplies of API for the commercialization of Ocaliva for PBC and, if approved, OCA for liver
fibrosis  due  to  NASH  that  we  believe  will  be  sufficient  to  meet  our  requirements  during  the  initial  stages  of  a  potential
NASH launch, we may not be able to procure sufficient supplies of API on an ongoing basis. If these suppliers are unable
to  provide  adequate  supply,  we  may  not  be  able  to  meet  our  long-term  commercial  supply  requirements  of  API  for  the
manufacture of Ocaliva or, if approved, OCA for liver fibrosis due to NASH or other indications on acceptable terms, or at
all.  We  do  not  have  agreements  for  long-term  supplies  of  any  of  our  product  candidates  other  than  OCA.  We  currently
obtain  supplies  and  services  relating  to  our  other  product  candidates  from  our  third-party  contract  manufacturers  on  a
purchase order basis.

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The  facilities  used  by  any  contract  manufacturer  to  manufacture  OCA  or  any  of  our  other  product  candidates  are
subject to inspection by the FDA and regulators in other jurisdictions. We are completely dependent on these third-party
manufacturers for compliance with the requirements of U.S. and non-U.S. regulators for the manufacture of our finished
products,  including  Ocaliva.  If  our  manufacturers  are  unable  to  meet  our  requirements  in  accordance  with  our  product
specifications  and  applicable  current  Good  Manufacturing  Practices  (“cGMP”)  requirements,  our  products  or  product
candidates  will  not  be  approved  or,  if  already  approved,  may  be  subject  to  recall.  In  addition,  if  COVID-19  or  related
public  health  safety  measures  prevent  the  FDA,  EMA  or  other  relevant  regulators  from  conducting  manufacturing
inspections or other regulatory activities with respect to manufacturing, it could significantly impact the ability of the FDA,
EMA or such other regulators to timely review and process our regulatory submissions, which could have a material and
adverse effect on our business and financial condition.

Reliance on third-party manufacturers entails risks to which we would not be subject if we manufactured our product

candidates and products ourselves, including:

● the possibility that we are unable to enter into or renew our manufacturing agreements with third parties on

acceptable terms, or at all;

● the possible termination, breach or non-performance by our third-party manufacturers of our manufacturing

agreements based on factors beyond our control; and

● our  inability  to  timely  identify  and  qualify  a  replacement  for  any  of  our  third-party  manufacturers  in  the
event any such third-party manufacturer fails to meet our product requirements or following the termination,
expiration or nonrenewal of our agreements with such third-party manufacturer.

Any of these factors could disrupt the supply of our product candidates or approved products, cause us to incur higher
costs, delay the approval of our product candidates or prevent or disrupt the commercialization of our approved products.
Furthermore,  if  any  of  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  are  approved  and  our
contract manufacturers fail to deliver the required commercial quantities of API or finished product on a timely basis and at
commercially reasonable prices and we are unable to find one or more replacement manufacturers capable of production at
a substantially equivalent cost, in substantially equivalent volumes and quality and on a timely basis, we would likely be
unable  to  meet  demand  for  such  product  candidate  following  its  approval  and  could  lose  potential  revenue.  It  may  take
several  years  to  establish  an  alternative  long-term  source  of  supply  and  to  have  any  such  new  source  approved  by  the
regulatory authorities that regulate our products in the United States, Europe and our other target markets.

We depend on third-party vendors and CROs for certain of our clinical trial and product development activities. If any
of these providers fail to comply with their contractual commitments or applicable regulatory obligations, including due to
COVID-19  and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel  and  in-person  interactions,
business closures and disruptions and other public health safety measures, our business could be materially and adversely
affected.  In  addition,  if  we  are  unable  to  maintain  our  relationship  with  any  one  or  more  of  these  providers,  we  could
experience a significant delay in both identifying another comparable provider and then contracting for its services, which
could  materially  and  adversely  affect  our  clinical  trial  and  product  development  efforts.  We  may  be  unable  to  retain  an
alternative provider on reasonable terms, or at all. Even if we locate an alternative provider, it is likely that such a provider
will need additional time to respond to our needs and may not provide the same type or level of services as the original
provider. Any third-party vendors and CROs that we retain are subject to the FDA’s regulatory requirements and similar
foreign standards and we do not have control over compliance with these regulations by these providers. The FDA, EMA
and other relevant regulatory authorities enforce these regulations through periodic inspections of trial sponsors, principal
investigators and trial sites. If these regulations are not adhered to by these providers, or if such providers fail to timely
correct  any  non-compliance  or  if  COVID-19  or  related  public  health  safety  measures  prevent  the  FDA,  EMA  or  other
relevant  regulatory  authorities  from  conducting  inspections  or  other  regulatory  activities,  the  commercialization  and
development of our product candidates or approved products could be delayed, which could materially and adversely harm
our business and financial condition.

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Even though we have received conditional approval of Ocaliva for PBC, we and our contract manufacturers are still
subject to strict, ongoing regulatory requirements.

Even though we have received conditional approval of Ocaliva for the treatment of PBC in combination with UDCA
in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate UDCA, we and our contract
manufacturers  are  subject  to  ongoing  regulatory  requirements  relating  to,  among  other  things,  Ocaliva’s  manufacturing,
packaging, labeling and storage. In addition, we and our contract manufacturers and our contract manufacturers’ facilities
are  required  to  comply  with  extensive  FDA  and  EMA  requirements  and  the  requirements  of  other  similar  regulatory
authorities, including requirements that quality control and manufacturing procedures conform to current cGMPs. As such,
we and our contract manufacturers are subject to periodic cGMP inspections and other inspections and audits required by
law  or  industry  standard  and  must  continue  to  expend  time,  money  and  effort  to  ensure  compliance  with  applicable
manufacturing, production and quality control requirements. We are also required to report certain adverse reactions and
production  problems,  if  any,  to  the  FDA,  EMA  and  other  similar  regulatory  authorities  and  to  comply  with  certain
requirements  concerning  advertising  and  promotion  for  our  products.  Promotional  communications  with  respect  to
prescription  drugs  are  subject  to  a  variety  of  legal  and  regulatory  restrictions  and  generally  must  be  consistent  with  the
information in the product’s approved label.

If a regulatory authority such as the FDA identifies previously unknown problems with one of our products, such as
adverse events of unanticipated severity or frequency or problems with the facility where the product is manufactured, or
disagrees with the promotion, marketing or labeling of one of our products, it may impose restrictions on that product or
us, including requiring withdrawal of the product from the market. In addition, if we or our contract manufacturers, other
third-party  vendors  or  collaborators  fail  to  comply  with  applicable  regulatory  requirements,  a  regulatory  agency  may,
among other things:

● issue Form 483 notices or Warning Letters, in the case of the FDA, or similar notices, in the case of other

regulatory agencies;

● mandate  modifications  to  our  promotional  materials  or  require  us  to  provide  corrective  information  to

healthcare practitioners;

● require us or our collaborators to enter into a consent decree or permanent injunction, which may include the
imposition of various fines, reimbursements for inspection costs, required due dates for specific actions and
penalties for noncompliance;

● recall our products;

● suspend any of our ongoing clinical studies;

● impose administrative, civil or criminal penalties;

● withdraw regulatory approval or require changes to our product label, including the inclusion of additional

warnings or changes to the approved indication;

● refuse  to  approve  pending  applications  or  supplements  to  approved  applications  filed  by  us  or  our

collaborators;

● impose  restrictions  on  our  operations  or  those  of  our  contract  manufacturers,  including  costly  new

manufacturing requirements; or

● seize or detain products.

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Risks Related to the Commercialization of Our Products

Sales of Ocaliva may be adversely affected by safety and labeling changes required by the FDA.

In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended weekly dose in such patients. As a result, in September 2017, we issued a DHCP letter and the FDA also
subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended  label  dosing.  Both  communications
remind  healthcare  providers  of  the  importance  of  the  recommended  reduced  dosing  of  Ocaliva  in  PBC  patients  with
moderate  or  severe  hepatic  impairment,  while  reiterating  the  importance  of  monitoring  PBC  patients  for  progression  of
their disease and the occurrence of liver-related adverse reactions. In February 2018, we announced that the Ocaliva label
in the United States had been updated by the FDA to include a boxed warning and a dosing table that reinforced the then-
existing  dosing  schedule  for  patients  with  Child-Pugh  Class  B  or  C  or  decompensated  cirrhosis.  In  addition,  the  FDA
issued an updated drug safety communication to accompany the revised label. We remain focused on the safety of all of the
patients  using  Ocaliva  within  and  outside  of  our  ongoing  clinical  studies  and  have  engaged  with  relevant  regulatory
authorities  to  ensure  that  the  Ocaliva  label  sufficiently  reinforces  the  importance  of  appropriate  dosing  in  patients  with
advanced cirrhosis.

The FDA has notified us that, in the course of its routine safety surveillance, in May 2020 the FDA began to evaluate a
newly identified safety signal, or NISS, regarding liver disorder for Ocaliva which the FDA classified as a potential risk.
The  FDA  has  informed  us  that  its  review  of  the  NISS  is  focused  on  a  subset  of  the  cirrhotic,  or  more  advanced,  PBC
patients who have taken Ocaliva. As part of our routine pharmacovigilance efforts, we worked with the FDA to reconcile
our  internal  safety  database  with  the  FDA  Adverse  Event  Reporting  System  database  and  completed  a  comprehensive
assessment of all available data, including data from our completed clinical trials, blinded reviews of ongoing clinical trial
data,  unblinded  reviews  of  certain  ongoing  clinical  trial  data  by  the  DMC,  post-marketing  data  and  natural  history  data,
which we submitted to the FDA and had a meeting earlier in 2021 to discuss. We are working with the FDA to align on
changes to the Ocaliva label regarding patients with the most advanced stages of PBC. Based on our communications with
the FDA, this update will come in the form of a safety labeling change. These communications are ongoing and any safety
concerns  associated  with  Ocaliva,  perceived  or  real,  may  adversely  affect  the  successful  development  and
commercialization of our product candidates and approved products, including Ocaliva, and materially and adversely affect
our business including future revenue generated by Ocaliva.

We are subject to uncertainty relating to pricing and reimbursement. Failure to obtain or maintain adequate coverage,
pricing and reimbursement for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future
approved products, if any, could have a material adverse impact on our ability to commercialize such products.

The availability and extent of coverage and reimbursement from governmental and private healthcare payors for our
products,  including  Ocaliva  for  PBC  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH,  and  our  ability  to  obtain
adequate pricing for such products are key factors that will affect our future commercial prospects. Government authorities
and third-party payors, such as private health insurers and health maintenance organizations, decide which drugs they will
cover  and  establish  payment  levels.  Sales  of  our  products  depend  and  will  depend  substantially,  both  domestically  and
internationally, on the extent to which their cost will be paid by health maintenance, managed care, pharmacy benefit and
similar healthcare management organizations or reimbursed by government health administration authorities, private health
coverage  insurers  and  other  third-party  payors.  Accordingly,  the  coverage  and  reimbursement  decisions  of  such
governmental and private healthcare payors could reduce the demand for, or the price paid for, our products. If these payors
do  not  consider  our  products  to  be  cost-effective  alone,  or  relative  to  other  approved  therapies,  they  may  not  cover  our
products or, if they do, they may apply utilization management restrictions, high patient cost-sharing obligations, or restrict
the level of reimbursement.

Third-party payors are increasingly challenging the prices charged for pharmaceuticals products, and many also limit
reimbursement for newly-approved products and indications. Third-party payors often attempt to contain healthcare costs
by  demanding  price  discounts  or  rebates  and  limiting  both  the  types  and  variety  of  drugs  that  they  will  cover  and  the
amounts that they will pay for drugs. As a result, they may not provide adequate payment for our products. Similarly, the

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containment of healthcare costs has become a priority for federal and state governments and the pricing of pharmaceutical
products  has  been  a  focus  in  this  effort.  The  U.S.  government,  state  legislatures  and  foreign  governments  have  shown
significant  interest  in  implementing  cost-containment  programs,  including  price  controls,  restrictions  on  reimbursement,
requirements  for  substitution  of  generic  products  and  requirements  to  demonstrate  a  specific  degree  of  improvement  in
terms of medical benefit compared to existing therapies. Adoption of price controls and cost-containment measures, and
adoption of more restrictive policies in jurisdictions with existing controls and measures, could adversely affect our ability
to successfully commercialize our products. In addition, we may be required to conduct post-marketing studies in order to
demonstrate  the  cost-effectiveness  of  our  products  to  payors’  satisfaction.  Such  studies  might  require  us  to  commit  a
significant amount of management’s time and our financial and other resources and our products might not ultimately be
considered cost-effective.

We  do  not  know  if  Ocaliva  for  PBC  will  obtain  and  maintain  broad  acceptance  from  third-party  payors  in  the
jurisdictions in which it is, or may in the future be, approved. In addition, even if OCA for liver fibrosis due to NASH is
approved,  we  do  not  know  if  it  will  obtain  and  maintain  broad  acceptance  from  third-party  payors.  The  coverage
determination process is a time-consuming and costly process that requires us to provide scientific and clinical support for
the  use  of  Ocaliva  for  PBC  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH  to  each  payor  separately,  with  no
assurance  that  coverage  will  be  obtained  or  maintained.  The  market  for  a  drug  depends  significantly  on  access  to  third-
party payors’ drug formularies, or lists of medications for which third-party payors provide coverage and reimbursement.
Third-party payors may refuse to include a particular drug in their formularies or restrict patient access to a branded drug
when a less costly generic equivalent or other alternative is available, even if not approved for the indication for which the
branded  drug  is  approved.  Due  to  there  being  no  uniform  policy  of  coverage  and  reimbursement  in  the  United  States
among commercial payors, coverage and reimbursement for pharmaceutical products may differ significantly from payor
to payor. If we are unable to obtain and maintain adequate coverage from third-party payors, the adoption of Ocaliva for
PBC and, if approved, OCA for liver fibrosis due to NASH by physicians and patients may be limited. This in turn could
affect our ability to successfully commercialize Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH and
have a material adverse impact our profitability, results of operations, financial condition and future success.

We cannot be certain that we will be able to obtain and maintain adequate coverage, pricing and reimbursement for our
products,  including  Ocaliva  for  PBC,  OCA  for  liver  fibrosis  due  to  NASH,  if  approved,  or  our  other  future  approved
products,  if  any.  If  coverage  or  reimbursement  is  not  available  or  is  available  on  a  limited  basis,  or  if  we  are  unable  to
obtain and maintain adequate pricing, we may not be able to successfully commercialize Ocaliva for PBC, OCA for liver
fibrosis due to NASH, if approved, or our other future approved products, if any.

Legislative and regulatory healthcare reform may adversely affect our business.

In  the  United  States,  the  Medicare  Prescription  Drug,  Improvement,  and  Modernization  Act  of  2003  (the  “MMA”)
changed  the  way  Medicare  covers  and  pays  for  pharmaceutical  products.  The  legislation  established  Medicare  Part  D,
which  expanded  Medicare  coverage  for  outpatient  prescription  drug  purchases  by  the  elderly  but  provided  authority  for
limiting the number of drugs that will be covered in any therapeutic class. The MMA also introduced a new reimbursement
methodology  based  on  average  sales  prices  for  physician-administered  drugs.  Any  negotiated  prices  for  our  products
covered by a Part D prescription drug plan will likely be lower than the prices we might otherwise obtain. Moreover, while
the MMA applies only to drug benefits for Medicare beneficiaries, private payors often follow Medicare coverage policy
and  payment  limitations  in  setting  their  own  payment  rates.  Any  reduction  in  payment  that  results  from  the  MMA  may
result in a similar reduction in payments from non-governmental payors.

In  March  2010,  the  Patient  Protection  and  Affordable  Care  Act,  as  amended  by  the  Health  Care  and  Education
Affordability  Reconciliation  Act  (collectively,  the  “ACA”),  became  law  in  the  United  States.  Among  other  things,  the
purpose of the ACA was to reduce the cost of healthcare and substantially change the way healthcare is financed by both
governmental and private insurers. The ACA requires discounts under the Medicare drug benefit program and increased
the rebates paid by pharmaceutical companies on drugs covered by Medicaid. The ACA also imposes an annual fee, which
increases each year, on sales by branded pharmaceutical manufacturers. Since its enactment, there have been a number of
judicial, executive and legislative challenges to the ACA, including tax legislation that removed the financial penalties for
people  who  do  not  carry  health  insurance  and  an  Executive  Order  signed  in  October  2017  by  former  President  Trump
directing federal agencies to modify how the ACA is implemented. There is still uncertainty over whether the ACA will

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undergo additional revisions, and we cannot predict the impact of any future modifications. Further, in December 2018, a
federal district court in Texas ruled that the entire ACA was unconstitutional because it could not be considered an exercise
of Congressional taxing authority following the repeal of the individual mandate penalties. In December 2019, a federal
court of appeals upheld the district court's decision that the ACA individual mandate was unconstitutional absent financial
penalties, but remanded the case back to the district court to determine whether the remaining provisions of the ACA were
nonetheless  valid.  However,  in  March  2020,  before  the  district  court  could  rule  on  the  ACA’s  remaining  provisions,  the
U.S. Supreme Court agreed to review the case and oral arguments were held in November 2020. A decision is expected
sometime  before  June  2021.  We  cannot  predict  the  outcome  of  this,  or  any  other,  litigation  regarding  the  ACA  or  the
impact it may have on our business.

Reimbursement in the European Union and many other territories must be negotiated on a country-by-country basis
and  in  many  countries  a  product  cannot  be  commercially  launched  until  reimbursement  is  approved.  The  timing  to
complete the negotiation process in each country is highly uncertain. Even after a price is negotiated, countries frequently
request or require adjustments to the price and other concessions over time or require approvals regionally. Reimbursement
agencies  in  Europe  are  often  more  conservative  than  those  in  the  United  States  and  the  reimbursement  process  is  often
slower  since  reimbursement  decisions  are  made  on  a  country-by-country  basis  and  may  involve  multiple  government
agencies in a given country. Prices for drugs in Europe are generally lower than in the United States and tend to decrease
over time.

The United States and several other jurisdictions are considering, or have already enacted, a number of legislative and
regulatory proposals to change their healthcare systems in ways that could affect our ability to sell our products profitably.
Among policy makers and payors in the United States and elsewhere, there is significant interest in promoting changes in
healthcare  systems  with  the  stated  goals  of  containing  healthcare  costs,  improving  quality  and/or  expanding  access  to
healthcare.  In  the  United  States,  the  pharmaceutical  industry  has  been  a  particular  focus  of  these  efforts  and  has  been
significantly affected by major legislative initiatives. We expect to experience pricing pressures in connection with the sale
of  Ocaliva  and  our  other  future  approved  products,  if  any,  due  to  the  trend  toward  managed  healthcare,  the  increasing
influence of health maintenance organizations and additional legislative proposals. Pricing pressures recently experienced
by the pharmaceutical industry may be further exacerbated by legislative and policy changes proposed or considered by the
executive  branch  and  the  United  States  Congress.  For  example,  in  June  2020,  the  Centers  for  Medicare  &  Medicaid
Services  released  a  proposed  rule  in  a  bid  to  update  and  expand  key  regulations  governing  the  Medicaid  Drug  Rebate
Program.  If  finalized  as  written,  these  changes  will  impact  manufacturers’  commercial  strategies,  government  payor
program  liabilities,  lifecycle  management  plans,  patient  assistance  regimes,  and  other  important  considerations.  In
November 2020, the Department of Health and Human Services finalized a rule that eliminates the safe harbor shielding
Medicare Part D rebates from the Anti-Kickback Statute and a rule that will tie certain Medicare Part B drug prices to those
paid by other countries. The rule is currently being challenged in litigation and we cannot predict the outcome of this, or
any other, litigation or the impact it may have on our business. Further, it is not known if the rule will be withdrawn by the
new President Biden administration. There have also been recent state legislative efforts to address drug costs, which have
generally  focused  on  increasing  transparency  around  drug  costs  or  limiting  drug  prices.  In  addition,  it  is  possible  that
additional  governmental  action  is  taken  to  address  pricing  concerns  arising  in  connection  with  COVID-19.  We  cannot
predict the success or impact of any such current or future federal or state legislative efforts.

Ocaliva and our other future approved products, if any, may not achieve broad market acceptance among physicians,
patients and healthcare payors, and revenues generated from their sales may be limited as a result.

The commercial success of Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, and our other future
approved products, if any, will depend upon their acceptance among the medical community, including third-party payors,
healthcare providers and professionals and customers, including patients and patient advocacy groups. In order for Ocaliva
to be commercially successful for PBC, we need to demonstrate its utility as a cost-effective treatment for PBC patients
who have an inadequate response to UDCA or who are unable to tolerate UDCA. Ocaliva also must be shown to be a safe
and  tolerable  treatment  in  a  commercial  use  setting  as  it  is  intended  to  be  a  lifetime  therapy  for  patients  eligible  for
treatment. We cannot be certain that Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future
approved  products,  if  any,  will  achieve  an  adequate  level  of  acceptance  among  the  medical  community,  including
physicians, healthcare payors and patients.

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In addition, we are closely evaluating the impact of COVID-19 on our ability to effectively market, sell and distribute
Ocaliva  for  PBC.  Our  field-based  employees  are  generally  working  remotely  and  are  interacting  with  healthcare
professionals  via  digital  communication  technologies  such  as,  where  appropriate,  video  conferences,  emails  and  phone
calls. Many of the healthcare professionals that we call on are working from home and facing additional demands on their
time due to COVID-19. We are experiencing increased competition for virtual appointments with healthcare professionals,
which may result in the cancellation of diagnostic, elective, specialty and other procedures and appointments to avoid non-
essential patient exposure to medical environments and potential infection with COVID-19 and to focus limited resources
and personnel capacity toward the treatment of COVID-19. Our increased utilization of virtual interactions and the reduced
quantity  of  such  interactions  during  the  COVID-19  pandemic,  may  reduce  the  effectiveness  of  our  sales  personnel  and
negatively affect physician awareness and sales of Ocaliva. In the fourth quarter of 2020, we continued to see a lower level
of  prescriptions  for  new  patients  than  we  did  prior  to  the  outbreak  of  COVID-19.  Although  new  patient  starts  currently
account for only a small percentage of total Ocaliva prescriptions, our future sales of Ocaliva could be negatively impacted
if  prescriptions  for  new  patients  do  not  return  to  levels  seen  prior  to  the  outbreak  of  COVID-19.  It  is  also  possible  that
COVID-19  may  negatively  affect  our  product  sales  in  the  future  due  to  patient  challenges  in  accessing  healthcare
providers,  significant  increases  in  unemployment  and  the  resulting  loss  of  individual  health  insurance  coverage,  and  an
inability to access government healthcare programs due to backlogs or other factors. As public health restrictions on travel
and in-person interactions are modified or relaxed, we may continue to face challenges that limit our ability to fully resume
in-person interactions, including the potential for additional outbreaks, limited access to personal protective equipment, the
need to navigate varying restrictions for entering healthcare facilities and employee illness and childcare obligations during
school closures. We also expect that the conversion of medical conferences to a virtual format may reduce our ability to
appropriately disseminate scientific information and conduct disease state education. The long-term effects of COVID-19
are unknown and it is possible that following the pandemic, healthcare institutions could alter their policies with respect to
in-person visits by pharmaceutical company representatives.

The degree of market acceptance of our approved products depends on a number of factors, including:

● limitations,  warnings,  precautions,  boxed  warnings,  contraindications,  restrictions  or  other  statements
contained in the product labels of our products, or any risk mitigation programs such as a REMS required for
our products by the FDA, EMA or other relevant regulatory authorities;

● changes in the standard of care or availability of alternative therapies at similar or lower costs for the targeted

indications for any of our products, such as UDCA for the treatment of PBC;

● limitations in the approved indications for our products;

● demonstrated and perceived clinical safety and efficacy compared to competitive products;

● a lack of adverse side effects, including deaths and other serious adverse events;

● sales, marketing and distribution support;

● the availability of reimbursement from managed care plans and other third-party payors;

● the timing of the market introduction of competitive products;

● the degree of cost-effectiveness;

● availability of alternative therapies at similar or lower cost, including generic and over-the-counter products;

● the  extent  to  which  our  products  are  approved  for  inclusion  on  formularies  of  hospitals  and  managed  care

organizations;

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● whether  and  to  what  extent  our  products  are  recommended  under  physician  treatment  guidelines  for  the

treatment of the indications for which we have received regulatory approval;

● adverse publicity concerning our products or favorable publicity concerning competitive products;

● the convenience and ease of administration of our products;

● potential product liability claims; and

● the  effects  of  COVID-19  and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel

and in-person interactions, business closures and disruptions and other public health safety measures.

In addition, the potential market opportunity for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved,
and our other future approved products, if any, is difficult to precisely estimate. For example, our estimates of the potential
market opportunity for Ocaliva for PBC include a number of key assumptions related to prevalence rates, patients’ access
to healthcare, diagnosis rates and patients’ response to or tolerance of Ocaliva, which are based on available literature and
epidemiology  research  in  PBC,  our  industry  knowledge  gained  through  market  research  and  other  methods,  industry
publications, third-party research reports and other surveys. While we believe that our internal assumptions are reasonable,
no independent source has verified such assumptions. If any of these assumptions prove to be inaccurate, then the actual
market for Ocaliva for PBC could be smaller than our estimates of our potential market opportunity. If the actual market
opportunity for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future approved products,
if any, is smaller than we expect, our product revenue may be limited and our financial condition and results of operations
may be materially and adversely affected.

If Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future approved products, if any, do
not achieve an adequate level of acceptance among the medical community, including physicians, healthcare payors and
patients,  sufficient  revenue  may  not  be  generated  from  these  products  and  we  may  not  become  or  remain  profitable.  In
addition, our efforts to educate the medical community and third-party payors on the benefits of Ocaliva for PBC, OCA for
liver fibrosis due to NASH, if approved, and our other future approved products, if any, may require significant resources
and may never be successful.

We  have  limited  sales,  marketing  and  distribution  experience  and  we  will  need  to  continue  to  invest  in  significant
additional resources to develop those capabilities or enter into acceptable third-party sales and marketing arrangements.

We  have  limited  sales,  marketing  and  distribution  experience  as  a  commercial  organization.  Ocaliva  is  our  first
approved product and the commercial launch of Ocaliva for PBC was our first product launch. We are commercializing
Ocaliva for PBC using a combination of our internal commercial organization and third-party distributors, depending on
the jurisdiction. We are developing our commercialization strategy for OCA for liver fibrosis due to NASH, if approved,
and  have  not  yet  decided  on  our  commercialization  strategy  for  OCA  for  other  indications  or  for  our  other  product
candidates, in each case, if approved. To develop internal sales, distribution and marketing capabilities, we have invested,
and expect to continue to invest, significant amounts of financial and management resources.

Recruiting and training a commercial organization is expensive, time-consuming and could delay any product launch.
We can provide no assurance that we will correctly forecast the needs for growth of our commercial organization given our
reliance  on  approvals  from  regulatory  authorities  for  our  product  candidates.  If  the  commercial  launch  of  a  product  for
which we recruit a sales force and establish marketing and distribution capabilities is delayed or does not occur for any
reason, we would have prematurely or unnecessarily incurred these commercialization expenses. This may be costly, and
our  investment  could  be  lost  if  we  cannot  retain  or  reposition  our  sales  and  marketing  personnel.  For  example,  we
expanded our commercial organization in anticipation of a potential U.S. commercial launch of OCA for liver fibrosis due
to NASH. However, in June 2020, we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis
due to NASH. Although we are in discussions with the FDA with respect to the potential resubmission of our NDA seeking
accelerated  approval  of  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH,  there  is  no  assurance  that  we  will  be
successful or that OCA will be approved for liver fibrosis due to NASH on an accelerated basis, or at all. Accordingly, our

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previously  anticipated  U.S.  commercial  launch  of  OCA  for  liver  fibrosis  due  to  NASH  has  been  postponed,  we  do  not
expect to generate revenues for this indication until it has been approved, and we may incur significantly greater costs than
previously anticipated in connection with the development of OCA for liver fibrosis due to NASH. In August 2020, we
adopted  the  2020  Workforce  Plan  to  reduce  our  workforce  in  light  of  the  receipt  of  the  CRL  from  the  FDA.  The  2020
Workforce Plan sought to streamline our operations and reduce operating expenses, while maintaining the critical resources
needed to continue to support the NASH and PBC clinical programs, pursue the approval of OCA for the treatment of liver
fibrosis  due  to  NASH  and  support  our  successful  PBC  business.  The  2020  Workforce  Plan  resulted  in  a  workforce
reduction of approximately 25%, or approximately 170 employees, and largely affected the commercial infrastructure we
had  developed  in  anticipation  of  a  potential  U.S.  commercial  launch  of  OCA  for  liver  fibrosis  due  to  NASH.  The  2020
Workforce  Plan  was  implemented  during  the  third  quarter  of  2020,  immediately  after  its  announcement,  and  was
substantially completed by the end of 2020.

For approved products where we decide to perform sales, marketing and distribution functions ourselves or through

third parties, we could face a number of additional risks, including:

● we or our third-party sales collaborators may not be able to attract and build, or retain, an effective marketing

or sales force;

● the  cost  of  securing  or  establishing  a  marketing  or  sales  force  may  exceed  the  revenues  generated  by  our

products; and

● our sales and marketing efforts may not be successful.

We may utilize the services of third-party collaborators in certain jurisdictions. We may have limited or no control over
the sales, marketing and distribution activities of these third parties, and our future revenues may depend heavily on their
success.

In addition, the effects of COVID-19 and related government-imposed shelter-in-place mandates, restrictions on travel
and  in-person  interactions,  business  closures  and  disruptions  and  other  public  health  safety  measures  may  negatively
impact our and our third-party collaborators’ productivity, limit the conduct of business operations and impair our and our
third-party collaborators’ ability to execute our sales, marketing and distribution strategy.

We could incur significant liability if it is determined that we have improperly promoted or are improperly promoting
Ocaliva for PBC or any of our product candidates prior to their approval.

Physicians are permitted to prescribe drug products for uses that are not described in the product’s labeling and that
differ from those approved by the FDA or other applicable regulatory agencies. Off-label uses are common across medical
specialties. Although the FDA and other regulatory agencies do not regulate a physician’s choice of treatments, the FDA
and other regulatory agencies do restrict communications on the subject of off-label use. Companies are not permitted to
promote  drugs  in  a  manner  inconsistent  with  applicable  regulatory  guidance.  The  FDA,  the  U.S.  Department  of  Justice
(“DOJ”) and other regulatory and enforcement authorities actively enforce laws and regulations prohibiting the improper
promotion of approved products, as well as the promotion of products for which marketing approval has not been obtained.
A company that is found to have improperly promoted off-label uses will be subject to significant liability, including civil
and  administrative  remedies  as  well  as  criminal  sanctions.  A  significant  number  of  pharmaceutical  companies  have
received inquiries or been the subject of investigations by various governmental authorities in the United States and abroad.
Both federal and state governments have levied large civil and criminal fines against companies for alleged improper off-
label promotion, as well as promotion that is determined to be false or misleading, even if related to approved indications.

While we have implemented a corporate compliance program based on what we believe are current best practices, we
cannot provide any assurance that governmental authorities, including the DOJ, SEC or FDA, will find that our business
practices  comply  with  all  current  or  future  administrative  or  judicial  interpretations  of  potentially  applicable  laws  and
regulations.  In  addition,  government  and  regulatory  agencies  may  hold  us  responsible  for  any  actions  by  our  sales
representatives and other employees or contingent workers to the extent that they do not comply with applicable laws and
regulations. If we fail to comply with any of these laws and regulations, we could be subject to a range of penalties,

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including  the  issuance  of  an  untitled  letter,  a  warning  letter,  injunction,  seizure,  criminal  and  significant  civil  penalties,
fines, damages, disgorgement, curtailment or restructuring of our operations, exclusion, disqualification or debarment from
participation in federally- or state-funded healthcare programs or other sanctions or litigation, any of which could have a
material adverse impact on our business, financial condition and results of operations.

If  we  market  products  in  a  manner  that  violates  healthcare  fraud  and  abuse  laws,  or  if  we  violate  government  price
reporting or physician payment disclosure laws, we may be subject to civil or criminal penalties.

In addition to FDA restrictions on the marketing of pharmaceutical products, several other types of state and federal
healthcare  laws,  commonly  referred  to  as  “fraud  and  abuse”  laws,  have  been  applied  in  recent  years  to  restrict  certain
marketing practices in the pharmaceutical industry. Other jurisdictions including Europe have similar laws and are enacting
more stringent regulations. These laws include false claims and anti-kickback statutes. If we market our products and our
products  are  paid  for  by  governmental  programs,  it  is  possible  that  some  of  our  business  activities  could  be  subject  to
challenge under one or more of these laws.

Federal  false  claims  laws  generally  prohibit  anyone  from  knowingly  and  willingly  presenting,  or  causing  to  be
presented, any claims for the payment for goods (including drugs) or services to third-party payers (including Medicare and
Medicaid) that are false or fraudulent. The federal civil monetary penalties statute, likewise, imposes penalties against any
person or entity that, among other things, is determined to have presented or caused to be presented a claim to a federal
health program that the person knows or should know is for an item or service that was not provided as claimed or is false
or fraudulent.

The federal healthcare program anti-kickback statute prohibits, among other things, knowingly and willfully offering,
paying,  soliciting  or  receiving  remuneration  to  generate  business,  including  the  purchase  or  prescription  of  a  particular
product covered by Medicare, Medicaid or other federally financed healthcare programs. This statute has been interpreted
to apply to arrangements between pharmaceutical manufacturers on the one hand and prescribers, purchasers or formulary
managers  on  the  other.  Although  there  are  several  statutory  exemptions  and  regulatory  safe  harbors  protecting  certain
common  activities  from  prosecution,  the  exemptions  and  safe  harbors  are  drawn  narrowly,  and  practices  that  involve
remuneration intended to induce prescribing, purchasing or recommending may be subject to scrutiny if they do not qualify
for an exemption or safe harbor. In addition, such exemptions and safe harbors are subject to change from time to time.

The Health Insurance Portability and Accountability Act of 1996 (as amended by the Health Information Technology
for  Economic  and  Clinical  Health  Act,  “HIPAA”)  created  additional  federal  criminal  statutes  that  prohibit,  among  other
things, knowingly and willfully executing, or attempting to execute, a scheme to defraud any healthcare benefit program,
or obtain, by means of false or fraudulent pretenses, or promises, any of the money or property owned by, or under the
custody or control of, any healthcare benefit program, regardless of the payor (e.g., public or private) and knowingly and
willfully  falsifying,  concealing  or  covering  up  by  any  trick  or  device  a  material  fact  or  making  any  materially  false
statement, in connection with the delivery of, or payment for, healthcare benefits, items or services. HIPAA also imposes
significant requirements on the receipt and transfer of protected health information.

In  addition,  the  federal  transparency  requirements  under  the  Physician  Payments  Sunshine  Act  require  certain
manufacturers of drugs, including us, for which payment is available under certain federal healthcare programs annually to
report  information  related  to  payments  and  other  transfers  of  value  to  physicians  and  teaching  hospitals,  and  physician
ownership and investment interests. Beginning in 2021, the federal reporting requirements will also apply to payments and
transfers  of  value  to  physician  assistants,  nurse  practitioners,  clinical  nurse  specialists,  certified  registered  nurse
anesthetists and anesthesiologist assistants, and certified nurse-midwives.

Finally, we must offer discounted pricing or rebates on Ocaliva and our future approved products, if any, under various
federal and state healthcare programs, and report specific prices to government agencies under healthcare programs. The
calculations necessary to determine the prices reported are complex and the failure to report prices accurately may expose
us to significant penalties.

There  are  foreign  and  state  law  equivalents  of  these  laws  and  regulations,  such  as  anti-kickback,  false  claims,

transparency and data privacy and security laws, to which we are currently and/or may in the future be subject. We may

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also  be  subject  to  foreign  and  state  laws  that  require  manufacturers  to  report  information  related  to  payments  and  other
transfers of value to physicians and other healthcare providers or marketing expenditures. Many of these laws differ from
each other in significant ways, thus increasing the cost and complexity of our compliance efforts.

A number of pharmaceutical and other healthcare companies have been prosecuted under these laws for a variety of
promotional and marketing activities, including providing free trips, free goods, sham consulting fees and grants and other
monetary benefits to prescribers; reporting inflated average wholesale prices that were then used by federal programs to set
reimbursement  rates;  engaging  in  improper  promotional  activities;  and  submitting  inflated  best  price  information  to  the
Medicaid Drug Rebate Program to reduce liability for Medicaid rebates.

If  we  or  our  operations  are  found  to  be  in  violation  of  any  of  the  laws  described  above  or  any  other  governmental
regulations  that  apply  to  us,  we  may  be  subject  to  penalties,  including  criminal  and  significant  civil  penalties,  damages,
fines, imprisonment, exclusion of products from reimbursement under United States federal or state healthcare programs,
and the curtailment or restructuring of our operations. Any penalties, damages, fines, curtailment or restructuring of our
operations  could  materially  and  adversely  affect  our  ability  to  operate  our  business  and  our  financial  results.  Although
compliance programs can mitigate the risk of investigation and prosecution for violations of these laws, the risks cannot be
entirely eliminated. Any action against us for violation of these laws, even if we successfully defend against it, could cause
us to incur significant legal expenses and divert our management’s attention from the operation of our business. Moreover,
achieving and sustaining compliance with these laws may prove costly.

We  may  not  be  successful  in  establishing,  implementing  and  maintaining  development  and  commercialization
collaborations, which could adversely affect our ability to develop certain of our product candidates and our financial
condition  and  operating  results.  If  any  strategic  collaborator  fails  to  perform  its  obligations  under,  or  terminates,  its
agreement with us, our business could be substantially harmed.

Developing  pharmaceutical  products,  conducting  clinical 

trials,  obtaining  regulatory  approval,  expanding
manufacturing capabilities and marketing approved products are expensive, complex and time-consuming undertakings. As
a result, we have in the past entered into, and may in the future seek to enter into, collaborations with third parties upon
whom we may rely for financial resources and for development, regulatory and commercialization expertise for selected
products  or  product  candidates  and  in  selected  jurisdictions.  We  may  establish  collaborations  with  respect  to  the
development and commercialization of OCA in various jurisdictions and for our other product candidates. Additionally, we
may enter into sales and marketing arrangements with third parties with respect to our approved products in all or certain
jurisdictions.

Our collaborators may fail to develop our product candidates or effectively commercialize our products for a variety of
reasons, including a lack of sufficient resources, a decision not to devote the necessary resources due to internal constraints,
such as limited cash or human resources, a change in strategic focus, a failure to obtain the necessary regulatory approvals
or business disruptions from COVID-19.

If we are unable to enter into new arrangements or maintain such arrangements on acceptable terms, or at all, we may
be  unable  to  effectively  market  and  sell  our  products  in  certain  of  our  target  markets.  We  expect  to  face  competition  in
seeking appropriate collaborators. Moreover, collaboration and similar arrangements are complex and time consuming to
negotiate, document and implement and they may require substantial resources to maintain. We may not be successful in
our efforts to establish and implement collaborations or other alternative arrangements for the development of our product
candidates.  When  we  collaborate  with  a  third  party  for  development  and  commercialization  of  a  product  candidate  or
approved product, we expect to relinquish some or all of the control over the future success of that product candidate or
approved  product  to  the  third  party.  Our  collaboration  partner  may  not  devote  sufficient  resources  to  development  or
commercialization  or  may  otherwise  fail  in  their  development  or  commercialization.  The  terms  of  any  collaboration  or
other arrangement that we establish may not be favorable to us. In addition, any collaboration that we enter into may be
unsuccessful.  In  some  cases,  we  may  be  responsible  for  continuing  preclinical  and  initial  clinical  development  of  a
partnered  product  candidate  or  research  program,  and  the  payment  we  receive  from  our  collaboration  partner  may  be
insufficient to cover the cost of this development. If we are unable to reach agreements with suitable collaborators, we may
incur increased costs and we may be forced to limit the number of products or product candidates we can commercially

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develop  or  the  territories  in  which  we  can  commercialize  them.  If  we  fail  to  achieve  successful  collaborations,  our
operating results and financial condition could be materially and adversely affected.

If we fail to develop OCA for additional indications such as NASH, our commercial opportunity will be limited.

To date, we have focused the majority of our development efforts on the development of OCA. One of our strategies is
to pursue clinical development of OCA for liver fibrosis due to NASH and other progressive non-viral liver diseases, to the
extent that we have sufficient funding to do so.

PBC is an orphan disease and the potential market size for Ocaliva for PBC is relatively limited. Furthermore, because
a  significant  proportion  of  PBC  patients  do  not  exhibit  any  symptoms  at  the  time  of  diagnosis,  PBC  may  be  left
undiagnosed for a significant period of time. Due to these factors, our ability to grow revenues will be dependent on our
ability  to  increase  market  share  and  successfully  develop  and  commercialize  OCA  for  the  treatment  of  additional
indications. In particular, we believe that our future success will depend in large part on the results of our development of
OCA  for  the  treatment  of  NASH.  Although  NASH  is  believed  to  be  one  of  the  most  prevalent  chronic  liver  diseases
worldwide,  NASH  may  be  left  undiagnosed  in  patients  for  a  long  period  of  time  and  a  definitive  diagnosis  of  NASH  is
often  based  on  a  histological  assessment  of  a  liver  biopsy,  which  impacts  the  ability  to  easily  identify  patients.
Furthermore,  even  if  we  are  successful  in  developing  and  obtaining  marketing  approval  of  OCA  for  the  treatment  of
NASH, we may not be commercially successful.

The completion of development, securing of approval and commercialization of OCA for additional indications such
as liver fibrosis due to NASH will require substantial additional funding, is subject to numerous risks and we may not be
successful.  We  cannot  provide  you  any  assurance  that  we  will  be  able  to  successfully  advance  any  of  these  indications
through the development process. Even if we receive regulatory approval to market OCA for the treatment of liver fibrosis
due  to  NASH  or  any  other  additional  indications,  we  cannot  assure  you  that  any  such  additional  indications  will  be
successfully  commercialized,  widely  accepted  in  the  marketplace  or  more  effective  than  other  commercially  available
alternatives.  If  we  are  unable  to  successfully  develop  and  commercialize  OCA  for  liver  fibrosis  due  to  NASH  or  other
additional indications, our commercial opportunity will be limited and our business prospects will suffer.

Risks Related to Our Business and Strategy

We depend on third-party contractors for a substantial portion of our operations and may not be able to control their
work as effectively as if we performed these functions ourselves.

We outsource and plan to continue to outsource substantial portions of our operations to third-party service providers,
including  CROs  for  certain  of  our  clinical  trial  and  product  development  activities,  and  contract  manufacturers  for  the
production of API and finished drug product for our commercial sales, clinical trials and preclinical studies. We will likely
also use the services of third-party vendors in connection with our future commercialization activities, including product
sales,  marketing  and  distribution.  Our  agreements  with  third-party  service  providers  are  typically  on  a  study-by-study
and/or  project-by-project  basis.  Typically,  we  may  terminate  these  agreements  with  notice  and  are  responsible  for  the
supplier’s previously incurred costs. In addition, a number of third-party service providers that we retain will be subject to
the FDA’s and EMA’s regulatory requirements and similar standards outside of the United States and Europe and we do not
have  control  over  compliance  with  these  regulations  by  these  providers.  If  these  providers  do  not  adhere  to  applicable
governing  practices  and  standards,  the  commercialization  of  Ocaliva  and  our  other  approved  products,  if  any,  and  the
development  of  OCA  and  our  other  product  candidates  could  be  delayed  or  stopped,  which  could  severely  harm  our
business and financial condition.

Because we have relied on third parties, our internal capacity to perform these functions is limited. Outsourcing these
functions involves the risk that third parties may not perform to our standards, may not produce results in a timely manner
or  may  fail  to  perform  at  all.  In  addition,  the  use  of  third-party  service  providers  requires  us  to  disclose  our  proprietary
information to these parties, which could increase the risk that this information will be misappropriated. There are a limited
number  of  third-party  service  providers  that  have  the  specialized  expertise  required  to  achieve  our  business  objectives.
Identifying, qualifying and managing the performance of third-party service providers can be difficult, time-consuming and
cause delays in our development programs. Despite our growth, we have limited internal resources available to identify

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and  monitor  third-party  service  providers.  To  the  extent  we  are  unable  to  identify,  retain  and  successfully  manage  the
performance of third-party service providers, our business may be materially and adversely affected. We may further be
subject to the imposition of civil or criminal penalties if our third party service providers violate applicable law.

Our third-party service providers generally are not prohibited from providing their services to other biopharmaceutical
companies,  including  companies  that  currently  or  may  in  the  future  compete  with  us.  For  example,  certain  of  our  third-
party service providers and consultants may be able to develop intellectual property to which we do not have rights under
our  agreements  and  that  may  eventually  be  used  to  develop  products  that  compete  with  our  products.  Although  we
generally  have  confidentiality  and  non-disclosure  agreements  in  place  with  our  third-party  service  providers  and
consultants,  such  third  parties  may  be  able  to  provide  services  to  other  companies  without  violating  the  terms  of  our
agreements. In addition, although we may seek to enter into non-compete arrangements with our key third-party service
providers,  such  arrangements  are  difficult  to  negotiate  and  we  may  be  unable  to  successfully  enter  into  or  enforce  such
arrangements.

The  effects  of  COVID-19  and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel  and  in-
person interactions, business closures and disruptions and other public health safety measures may negatively impact our
and our third-party service providers’ productivity, limit the conduct of business operations and impair our and our third-
party service providers’ ability to conduct operations.

We  face  rapid  technological  change  and  competition  from  other  biotechnology  and  pharmaceutical  companies.  Our
operating results will suffer if we fail to compete effectively.

The  biotechnology  and  pharmaceutical  industries  are  intensely  competitive  and  subject  to  rapid  and  significant
technological  change.  We  have  competitors  in  the  United  States,  Europe  and  other  jurisdictions,  including  major
multinational pharmaceutical companies, established biotechnology companies, specialty pharmaceutical and generic drug
companies and universities and other research institutions. Many of our competitors have financial, sales and marketing,
manufacturing and distribution, legal, regulatory and product development resources substantially greater than ours. Large
pharmaceutical  companies,  in  particular,  have  extensive  experience  in  research,  clinical  testing,  obtaining  regulatory
approvals, recruiting patients and manufacturing pharmaceutical products. These companies also have significantly greater
sales  and  marketing  capabilities  and  often  have  collaborative  arrangements  in  our  target  markets.  Established
pharmaceutical companies may also invest heavily to accelerate discovery and development of novel compounds or to in-
license novel compounds that could make our products or product candidates obsolete. As a result of all of these factors,
our competitors may succeed in obtaining patent protection and/or FDA, EMA or other regulatory approval or discovering,
developing  and  commercializing  drugs  for  the  diseases  that  we  are  targeting  before  we  do.  Smaller  or  early-stage
companies  may  also  prove  to  be  significant  competitors,  particularly  through  collaborative  arrangements  with  large,
established companies.

Some of the pharmaceutical and biotechnology companies that we may compete with include 89bio, Inc., AbbVie Inc.,
Acorda Therapeutics, Inc., Affimune Limited, Akcea Therapeutics, Inc., Akero Therapeutics, Inc., Albireo Pharma, Inc.,
Altimmune,  Inc.,  Arrowhead  Pharmaceuticals,  Inc.,  AstraZeneca  plc,  Blade  Therapeutics,  Inc.,  Boehringer  Ingelheim
GmbH,  Bristol-Myers  Squibb  Company,  Can-Fite  BioPharma  Ltd.,  Cirius  Therapeutics,  Inc.,  Corcept  Therapeutics
Incorporated, CymaBay Therapeutics, Inc., Dr. Falk Pharma GmbH, Durect Corporation, Eli Lilly and Company, Enanta
Pharmaceuticals, Inc., Forma Therapeutics, Inc. Galectin Therapeutics Inc., Galecto Biotech AB, Galmed Pharmaceuticals
Ltd., Genfit SA, Genkyotex, Gilead Sciences, Inc., GlaxoSmithKline plc, GRI Bio, Inc., Hanmi Pharmaceutical Co., Ltd.,
Hepion Pharmaceuticals, Inc., HighTide Therapeutics Inc., Immuron Limited, Inventiva, Ionis Pharmaceuticals, Inc., Kowa
Company,  Ltd.,  Lipocine  Inc.,  Madrigal  Pharmaceuticals,  Inc.,  MediciNova,  Inc.,  Metacrine,  Inc.,  Mitsubishi  Tanabe
Pharma  Corporation,  Nash  Pharmaceuticals  Inc.,  NGM  Biopharmaceuticals,  Inc.,  NorthSea  Therapeutics  B.V.,  Novartis
AG, Novo Nordisk A/S, NuSirt Biopharma, Inc., Oramed Pharmaceuticals Inc., Pfizer Inc., Poxel SA, Sagimet Biosciences
Inc., Second Genome, Inc., Sinew Pharma Inc., Terns Pharmaceuticals, Inc., Theratechnologies, Inc., Viking Therapeutics,
Inc., Yagrit International Ltd and Zydus Pharmaceuticals (USA) Inc. Ocaliva competes with UDCA (or ursodiol), a first-
line  therapy  approved  for  the  treatment  of  PBC  that  is  available  generically  at  a  significantly  lower  cost  than  Ocaliva.
Although we have a license to develop and commercialize bezafibrate in the United States, bezafibrate has been studied in
multiple clinical trials for the treatment of liver diseases including PBC and NASH outside of the United States. Genfit’s
elafibranor and CymaBay’s seladelpar are in late-stage studies for treatment of PBC. Novo Nordisk’s

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semaglutide, Madrigal’s resmetirom, and Inventiva’s lanifibranor are currently in late-stage development for treatment of
NASH.

In  addition,  many  universities  and  private  and  public  research  institutions  may  become  active  in  our  target  disease
areas. The results from our clinical trials and the approval of Ocaliva for PBC have brought more attention to our targeted
indications  and  bile  acid  chemistry.  As  a  result,  we  believe  that  additional  companies  and  organizations  may  seek  to
compete with us in the future. Our competitors may succeed in developing, acquiring or licensing on an exclusive basis,
technologies and drug products that are more effective or less costly than OCA or any other product candidates that we are
currently  developing  or  that  we  may  develop,  which  could  render  our  products  or  product  candidates  obsolete  and
noncompetitive. Our ability to compete may also be affected because, in many cases, insurers or other third-party payors
seek to encourage the use of generic products.

Off-label uses of other potential treatments may limit the commercial potential of our products and product candidates,
especially given the pricing of Ocaliva and the anticipated pricing for our product candidates. For example, while fibrates
are  not  approved  for  use  in  PBC,  off-label  use  of  fibrate  drugs  has  been  reported.  In  NASH,  a  number  of  treatments,
including  vitamin  E  (an  antioxidant),  insulin  sensitizers  (e.g.,  metformin,  pioglitazone),  antihyperlipidemic  agents  (e.g.,
gemfibrozil), pentoxifylline and UDCA, are used off-label. Although none of these treatments have been clearly shown in
clinical trials to alter the course of the disease, in a previous study conducted by the NASH Clinical Research Network,
improvements in certain histological measures of NASH were reported with vitamin E and pioglitazone.

We believe that our ability to successfully compete will depend on, among other things:

● the results of our and our strategic collaborators’ clinical trials and preclinical studies;

● our ability to recruit, enroll and retain patients for our clinical trials;

● the  efficacy,  safety  and  tolerability  of  Ocaliva,  OCA  for  liver  fibrosis  due  to  NASH,  if  approved,  and  our

other future approved products, if any;

● the speed at which we develop our product candidates;

● our ability to design and successfully execute appropriate clinical trials;

● our ability to maintain productive relationships with regulatory authorities;

● the timing and scope of regulatory approvals, if any;

● our ability to commercialize and market Ocaliva, OCA for liver fibrosis due to NASH, if approved, and our

other future approved products, if any;

● the price of our products;

● our  ability  to  obtain  adequate  levels  of  reimbursement  under  private  and  governmental  health  insurance

plans, including Medicare;

● our ability to protect our intellectual property rights related to our products;

● our ability to manufacture and sell commercial quantities of Ocaliva, OCA for liver fibrosis due to NASH, if

approved, and our other future approved products, if any, to the market; and

● the acceptance of our products by physicians and other healthcare providers.

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If our competitors market products that are more effective or safe or less expensive than our products or that reach the
market sooner than our products, we may not achieve commercial success. In addition, the biopharmaceutical industry is
characterized  by  rapid  technological  change.  Because  our  research  approach  integrates  many  technologies,  it  may  be
difficult for us to stay abreast of the rapid changes in other technologies. If we fail to stay at the forefront of technological
change, we may be unable to compete effectively. Technological advances or products developed by our competitors may
render our technologies, products or product candidates obsolete, less competitive or not economical.

A  variety  of  risks  associated  with  our  international  business  operations  and  our  planned  international  business
relationships could materially and adversely affect our business.

We  have  formed  a  number  of  subsidiaries  in  jurisdictions  outside  of  the  United  States  in  connection  with  or  in
anticipation of our commercial or other business activities in those jurisdictions. We are commercializing Ocaliva for PBC
using  a  combination  of  our  internal  commercial  organization  and  third-party  distributors,  depending  on  the  jurisdiction.
Our  variety  of  international  operations  and  business  relationships  subject  us  to  additional  risks  that  may  materially  and
adversely affect our business and ability to attain or sustain profitability, including:

● the  enhanced  anti-bribery  and  anti-corruption  regimes  now  implemented  in  most  European  Union  member
states and elsewhere, including the UK Bribery Act (thought to be one of the strictest anti-bribery laws in the
world) and the escalation of investigations and prosecutions pursuant to such laws;

● compliance with complex import and export control laws;

● restrictions on direct investments by foreign entities and country-specific trade restrictions;

● differing  regulatory  requirements  for  medicine  approvals  and  access  to  medicines  across  our  various
international markets and as a result the potential inability to obtain any necessary foreign regulatory, pricing
or reimbursement approvals for our products in a timely manner, or at all;

● variances  in  payment  terms  and  uncertainty  regarding  the  collectability  of  accounts  receivable  from  our

counterparties in our international business;

● difficulties in staffing and managing international operations;

● the potential for reduced protection for our intellectual property rights;

● the potential for third-party patent rights in countries outside of the United States;

● cross border trade of medicines by third parties within the European single market (for example the impact of

parallel trade within the European Economic Area);

● unexpected changes in tariffs, trade barriers and regulatory requirements and the imposition of governmental

controls;

● economic  weakness,  including  inflation,  or  political  instability,  particularly  in  non-U.S.  economies  and

markets, including countries in Europe;

● compliance  with  tax,  employment,  immigration  and  labor  laws  applicable  to  our  employees  working  or

traveling abroad;

● compliance with data protection laws, including regimes relating to cross-border transfer mechanisms;

● taxes in other countries;

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● foreign currency fluctuations, which could result in increased operating expenses and reduced revenue, and

other transactional risks incident to doing business in foreign countries;

● potential  for  production  shortages  resulting  from  events  affecting  raw  material  supply  or  manufacturing

capabilities abroad;

● business  interruptions  resulting  from  geo-political  actions,  including  war  and  terrorism,  global  health
emergencies,  such  as  COVID-19,  natural  disasters,  including  earthquakes,  volcanoes,  typhoons,  floods,
hurricanes and fires, or social unrest; and

● increasingly  complex  standards  for  complying  with  international  laws  and  regulations  that  may  differ

substantially from country to country and may conflict with corresponding U.S. laws and regulations.

Since the United Kingdom referendum on European Union membership in June 2016, there has been some political
and  economic  uncertainty,  including  in  the  regulatory  framework  applicable  to  the  operations  of  biotechnology  and
pharmaceutical companies, and this uncertainty may persist now that the impact of Brexit is being realized. There may be
disruption  and  uncertainties  in  the  free  movement  of  goods,  services  and  people  between  the  United  Kingdom  and  the
European Union, and at a more detailed level disruption to, and uncertainty regarding the application and interpretation of,
national  and  international  laws  and  regulations.  There  may  also  be  unforeseen  consequences  and  uncertainties  in  cross
border  trade  in  goods  and  services,  immigration  and  employment,  data  protection  and  digital  trade,  state  aid  and  fair
competition.  Over  the  last  few  years  our  international  business  has  undertaken  significant  planning  and  operational
readiness  work  for  Brexit  involving  business  functions  such  as  supply  chain,  quality,  finance/tax,  regulatory,
pharmacovigilance and legal. Brexit could materially change the regulatory regime applicable to our operations, including
with respect to Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH and our other product candidates.
Such  consequences  and  uncertainties  could  make  it  more  difficult  and  expensive  for  us  to  do  business,  complicate  our
clinical, manufacturing and regulatory strategies and impair our ability to obtain and maintain regulatory approval for, and,
if approved, commercialize, our products and product candidates in Europe. In addition, our ability to continue to conduct
our international operations out of the United Kingdom, where the headquarters for our international operations is located,
may  be  materially  and  adversely  affected.  While  we  have  undertaken  a  number  of  Brexit-related  contingency  planning
initiatives, we cannot make any assurances regarding the extent to which our business may be adversely affected thereby.

In  addition,  we  are  subject  to  the  anti-bribery  and  anticorruption  laws  of  the  United  States,  as  well  as  of  foreign
jurisdictions where we operate, including the U.S. Foreign Corrupt Practices Act and the UK Bribery Act. Generally, these
laws prohibit paying or offering anything of value to a foreign government official for the purpose of obtaining or retaining
business but they can also have a much wider, extraterritorial scope, as is the case with the UK Bribery Act (thought to be
one of the strictest anti-bribery laws in the world). U.S. and foreign regulators have increased their enforcement of anti-
bribery  and  anticorruption  laws  in  recent  years,  and  failure  to  comply  with  these  laws  could  result  in  various  adverse
consequences, including:

● the possible delay in approval or refusal to approve our product candidates;

● recalls, seizures or withdrawal from the market of an approved product;

● disruption in the supply or availability of our products or suspension of export or import privileges;

● the imposition of civil or criminal sanctions;

● the prosecution of executives overseeing our international operations; and

● damage to our reputation.

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Any significant impairment of our ability to develop our product candidates or sell our approved products outside of

the United States could adversely impact our business and financial results.

Our business and operations would suffer in the event of system failures, data breaches or violations of data protection
laws.

We are increasingly dependent on information technology systems and infrastructure, including mobile technologies,
to  operate  our  business.  In  the  ordinary  course  of  our  business,  we  collect,  process,  store  and  transmit  large  amounts  of
confidential  information,  including  intellectual  property,  proprietary  business  information  and  personal  information.  It  is
critical  that  we  do  so  in  a  secure  manner  to  maintain  the  confidentiality  and  integrity  of  such  information.  The  size  and
complexity  of  our  information  technology  systems,  and  those  of  third-party  vendors  with  whom  we  contract,  and  the
volume of data we retain, make such systems potentially vulnerable to breakdown, malicious intrusion, security breaches
and  other  cyber-attacks.  Information  security  risks  have  significantly  increased  in  recent  years  in  part  due  to  the
proliferation of new technologies and the increased sophistication and activities of organized crime, hackers, terrorists and
other external parties, including foreign state actors. Our information security systems and those of our third party vendors
are subject to laws and regulations, or may become subject to new laws and regulations, requiring that we enact certain
measures to protect the privacy and security of certain information we collect or use in our business. A security breach or
privacy violation that leads to disclosure or modification of, or prevents access to, personal information or other protected
information, whether caused by internal or external parties, could harm our reputation, compel us to comply with federal
and/or  state  breach  notification  laws  and  foreign  law  equivalents,  subject  us  to  notification  requirements  under  certain
agreements  with  third  parties,  subject  us  to  mandatory  corrective  action,  require  us  to  verify  the  correctness  of  database
contents  and  otherwise  subject  us  to  liability  under  laws  and  regulations  that  protect  personal  information,  resulting  in
increased  costs  or  loss  of  revenue.  Similarly,  the  loss  or  unauthorized  disclosure  of  clinical  trial  data  from  completed,
ongoing  or  planned  clinical  trials  could  prevent  us  from  obtaining  regulatory  approval  or  delay  our  regulatory  approval
efforts  and  significantly  increase  our  costs  to  recover  or  reproduce  the  data.  If  we  are  unable  to  prevent  such  security
breaches or privacy violations or implement satisfactory remedial measures, our operations could be disrupted, and we may
suffer  loss  of  reputation,  financial  loss  and  be  subject  to  regulatory  fines  and  penalties.  In  addition,  these  breaches  and
other inappropriate access can be difficult to detect, and any delay in identifying them may lead to increased harm of the
type described above. Moreover, the reliance on remote working technologies by our employees and third party partners
due  to  COVID-19  and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel  and  in-person
interactions and other public health safety measures and the prevalent use of mobile devices that access confidential and
personal information increases the risk of data security breaches, which could lead to the loss of confidential information,
personal information, trade secrets or other intellectual property. As cyber threats continue to evolve, we may be required
to expend significant additional resources to continue to modify or enhance our protective measures or to investigate and
remediate  any  information  security  vulnerabilities.  While  we  have  implemented  security  measures  to  protect  our  data
security and information technology systems, such measures may not prevent such events. Significant disruptions of our
information technology systems or breaches of data security could have a material adverse effect on our business, financial
condition and results of operations.

In  the  United  States,  numerous  federal  and  state  laws,  including,  without  limitation,  HIPAA  state  security  breach
notification  laws,  state  health  information  privacy  laws  and  federal  and  state  consumer  protection  laws,  govern  the
collection, use, disclosure and storage of personal information as well as consumer rights with regard to such information.
For example, California recently passed the California Consumer Privacy Act of 2018, which became effective on January
1,  2020  and  other  states  are  developing  similar  privacy  laws.  Various  foreign  countries  where  we  may  process  personal
information  also  have,  or  are  developing,  privacy  and  data  protection  laws  governing  the  collection,  use,  disclosure  and
storage of personal information.

In July 2016, U.S. and European Commission officials adopted a framework called the European Union-U.S. Privacy
Shield (the “EU Privacy Shield”) to govern transfers of personal data from the European Economic Area (“EEA”) to the
U.S. We adopted the European Union-U.S. Privacy Shield and have certified to its requirements since October 2016. We
also adopted the Swiss-U.S. Privacy Shield (the “Swiss Privacy Shield”) in order to legitimize the transfer of personal data
from Switzerland to the U.S. In May 2018, the General Data Protection Regulation (the “GDPR”) took effect in the EEA.
The  GDPR  imposes  more  stringent  data  protection  requirements,  and  provides  for  greater  penalties  for  noncompliance,
than previous EEA data protection legislation. In addition, although we have implemented certain measures as a result of

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Brexit to allow for the transfer of personal data between EEA member states and the United Kingdom, we may need to
develop additional mechanisms to permit for the transfer of this data. Implementation of the GDPR and other changes in
privacy  and  data  protection  laws  or  regulations  could  require  changes  to  certain  of  our  business  practices,  thereby
increasing our costs. While we are engaging in activities to comply with the GDPR requirements and other data protection
laws, we may be unsuccessful in these efforts.

On July 16, 2020, the Court of Justice of the European Union (“CJEU”) invalidated the EU Privacy Shield as a data
transfer  mechanism  for  transferring  personal  data  from  the  EEA  to  the  U.S.,  effective  immediately.  On  September  20,
2020, the Swiss Federal Data Protection and Information Commissioner invalidated the Swiss Privacy Shield. Therefore,
the EU Privacy Shield and the Swiss Privacy Shield no longer qualify as appropriate safeguards for the transfer of personal
data from the EEA or Switzerland to the U.S. and transfers made under those frameworks could attract regulatory scrutiny
and  penalties  for  non-compliance.  There  is  no  “grace  period”  to  allow  organizations  to  implement  an  alternative  data
transfer  mechanism  to  the  EU  Privacy  Shield  and  the  Swiss  Privacy  Shield.  While  the  European  Commission  approved
Standard Contractual Clauses (“SCCs”) and Binding Corporate Rules remain a valid mechanism to transfer personal data
to third countries outside the EEA and Switzerland, the CJEU's ruling has also imposed enhanced due diligence obligations
on organizations acting as data exporters and relying on SCCs to ensure that the laws of the country to which personal data
is  transferred  offers  a  level  of  data  protection  that  is  essentially  equivalent  to  the  EEA.  In  addition,  the  European
Commission is in the process of updating the SCCs to align them with the GDPR. As a result of the CJEU's ruling, the
status of the transfers of personal data from the EEA or Switzerland to the U.S. is currently subject to significant regulatory
uncertainty and we are actively monitoring developments in this area. To the extent we are not able to employ suitable data
transfer  mechanisms  to  facilitate  international  transfers  of  data,  our  ability  to  conduct  our  business  may  be  materially
adversely impacted.

The  legislative  and  regulatory  landscape  for  privacy  and  data  protection  continues  to  evolve,  and  there  has  been  an
increasing  amount  of  focus  on  privacy  and  data  protection  issues  that  may  affect  our  business.  There  is  a  degree  of
uncertainty associated with the legal and regulatory environment around privacy and data protection laws, which continue
to develop in ways we cannot predict, including with respect to evolving technologies, such as cloud computing. Privacy
and data protection laws may be interpreted and applied inconsistently from country to country and impose inconsistent or
conflicting requirements. As a result, our practices may not comply in the future with all such privacy and data protection
laws. Varying jurisdictional requirements could increase the costs and complexity of compliance or require us to change
our  business  practices  in  a  manner  adverse  to  our  business.  A  determination  that  we  have  violated  any  privacy  or  data
protection  laws  could  result  in  significant  damage  awards,  fines  and  other  penalties  that  could,  individually  or  in  the
aggregate,  materially  harm  our  business  and  reputation.  For  example,  administrative  fines  of  up  to  the  greater  of  €20
million  or  4%  of  our  global  turnover  may  be  imposed  for  breaches  of  the  GDPR.  We  may  also  be  liable  should  any
individual  who  has  suffered  financial  or  non-financial  damage  arising  from  our  infringement  of  the  GDPR  or  other
applicable data protection laws exercise his or her right to receive compensation against us.

In addition, our marketing activities and the marketing activities of any third parties on which we rely are subject to
various regulations, including privacy and data protection laws, consumer protection laws and competition laws. Such laws
may impair our ability, or the ability of third parties on which we rely, to collect information. Such regulations may have a
negative effect on businesses and may increase the potential civil liability and cost of operating our business.

We have significantly expanded our operations and plan to continue our expansion to support our future development
strategy for OCA for indications other than PBC, including liver fibrosis due to NASH. We may experience difficulties
in managing our significant growth.

We  have  significantly  expanded  our  operations,  including  the  size  of  our  employee  base,  as  we  pursue  our  future
development and commercialization strategy. As we advance our preclinical and clinical development programs for OCA
and  our  other  product  candidates,  seek  regulatory  approval  in  the  United  States  and  elsewhere  and  pursue  our
commercialization strategy, we may need to increase our product development, scientific, commercial and administrative
headcount.  Such  an  evolution  may  impact  our  strategic  focus  and  our  deployment  and  allocation  of  resources.  Our
management, personnel and systems may experience difficulty in adjusting to our growth and strategic focus.

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We  may  also  anticipate  needs  for  growth  that  do  not  materialize.  For  example,  we  expanded  our  commercial
organization in anticipation of a potential U.S. commercial launch of OCA for liver fibrosis due to NASH. However, in
June 2020, we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to NASH. Although
we are in discussions with the FDA with respect to the potential resubmission of our NDA seeking accelerated approval of
OCA for the treatment of liver fibrosis due to NASH, there is no assurance that we will be successful or that OCA will be
approved for liver fibrosis due to NASH on an accelerated basis, or at all. In August 2020, we adopted the 2020 Workforce
Plan  to  reduce  our  workforce  in  light  of  the  receipt  of  the  CRL  from  the  FDA.  The  2020  Workforce  Plan  sought  to
streamline  our  operations  and  reduce  operating  expenses,  while  maintaining  the  critical  resources  needed  to  continue  to
support the NASH and PBC clinical programs, pursue the approval of OCA for the treatment of liver fibrosis due to NASH
and support our successful PBC business. The 2020 Workforce Plan resulted in a workforce reduction of approximately
25%,  or  approximately  170  employees.  The  2020  Workforce  Plan  was  implemented  during  the  third  quarter  of  2020,
immediately after its announcement, and was substantially completed by the end of 2020. We can provide no assurance that
we will correctly forecast the needs for growth given our reliance on approvals from regulatory authorities for our product
candidates.

In addition, in order to continue to meet our obligations as a public company and to support our anticipated longer-
term growth, we may need to increase our general and administrative capabilities. We have also expanded our operations
geographically and formed a number of subsidiaries outside of the United States. In addition to our U.S. offices, we have
an office in London, which serves as the headquarters for our international operations, and regional offices in a number of
other countries, and we may further expand our geographical footprint. Our management, personnel and systems may not
be adequate to support this future growth. Furthermore, we may face a number of complexities, such as being subject to
national collective bargaining agreements for employees, in some of the countries in which we operate.

Our need to effectively manage our operations, growth and various projects requires that we:

● successfully attract and recruit new employees or consultants with the expertise and experience we require in

the United States, Europe and other jurisdictions;

● develop, expand or adjust our commercial infrastructure;

● manage our clinical programs effectively, which are often conducted at numerous domestic and international

clinical sites, and advance our other development efforts; and

● continue to improve our operational, financial and management controls, reporting systems and procedures.

If we are unable to successfully manage our growth and the increased complexity of our operations, our business may

be materially and adversely affected.

We  may  not  be  able  to  manage  our  business  effectively  if  we  are  unable  to  attract  and  retain  key  personnel  and
consultants.

We  may  not  be  able  to  attract  or  retain  qualified  personnel  and  consultants  due  to  the  intense  competition  for  such
individuals among biotechnology, pharmaceutical and other businesses. If we are not able to attract and retain necessary
personnel  and  consultants  to  accomplish  our  business  objectives,  we  may  experience  constraints  that  will  significantly
impede  the  achievement  of  our  development  and  commercial  objectives,  our  ability  to  raise  additional  capital  and  our
ability to implement our business strategy.

Our  industry  has  experienced  a  high  rate  of  turnover  of  management  personnel  in  recent  years.  We  are  highly
dependent on the development, regulatory, commercialization and business development expertise of the members of our
executive team, as well as other key employees and consultants. If we lose one or more of our executive officers or other
key employees or consultants, our ability to implement our business strategy successfully could be seriously harmed. Any
of our executive officers or other key employees or consultants may terminate their employment at any time and replacing
such individuals may be difficult and time-consuming because of the limited number of individuals in our industry with

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the necessary breadth of skills and experience. Competition to hire and retain employees and consultants from this limited
pool is intense, and we may be unable to hire, train, retain or motivate such individuals.

We  also  have  key  advisors  and  consultants  who  assist  us  in  operating  our  business.  These  advisors  are  not  our
employees  and  may  have  commitments  to,  or  consulting  or  advisory  contracts  with,  other  entities  that  may  limit  their
availability to us and such individuals typically will not enter into non-compete agreements with us. If a conflict of interest
arises between their work for us and their work for another entity, we may lose their services. In addition, our advisors may
assist other companies that compete with us.

Our  employees  may  engage  in  misconduct  or  other  improper  activities,  including  noncompliance  with  regulatory
standards and requirements and insider trading, which could significantly harm our business.

We are exposed to the risk of employee fraud or other misconduct. Misconduct by employees could include intentional
failures  to  comply  with  the  regulations  of  the  FDA,  the  SEC  or  other  domestic  or  foreign  regulators,  provide  accurate
information to the FDA, the SEC or other domestic or foreign regulators, comply with healthcare fraud and abuse laws and
regulations  in  the  United  States  and  abroad,  report  financial  information  or  data  accurately  or  disclose  unauthorized
activities to us. In particular, sales, marketing and business arrangements in the healthcare industry are subject to extensive
regulation in the United States and abroad intended to prevent fraud, misconduct, kickbacks, self-dealing and other abusive
practices.  Such  laws  and  regulations  may  restrict  or  prohibit  a  wide  range  of  pricing,  discounting,  marketing  and
promotion,  sales  commission,  customer  incentive  and  other  business  arrangements.  Employee  misconduct  could  also
involve the improper use of information obtained in the course of clinical trials, which could result in regulatory sanctions
and serious harm to our reputation. Misconduct and misappropriation of confidential information by our employees or third
parties  may  also  include  improper  trading  in  our  securities,  which  may  harm  our  reputation  and  result  in  enforcement
actions against us. We have adopted a global code of business conduct and implemented a corporate compliance program,
but it is not always possible to identify and deter employee misconduct, and the precautions we take to detect and prevent
this  activity  may  not  be  effective  in  controlling  unknown  or  unmanaged  risks  or  losses  or  in  protecting  us  from
governmental inquires, investigations or other actions or lawsuits stemming from a failure to comply with applicable laws
or regulations. The outcome of any such inquiry, investigation, action or lawsuit could have a significant negative impact
on our business, including as a result of the imposition of significant fines or other sanctions. In addition, the institution of
any such inquiry, investigation, action or lawsuit could negatively impact the market price of our securities.

We face potential product liability exposure, and if successful claims are brought against us, we may incur substantial
liability for our products or product candidates and may have to limit or suspend their use.

The use of our product candidates in clinical trials and the sale of any products for which we have obtained or may
obtain  marketing  approval,  such  as  Ocaliva  for  PBC,  expose  us  to  the  risk  of  product  liability  claims.  Product  liability
claims  may  be  brought  against  us  or  our  collaborators  by  participants  enrolled  in  our  clinical  trials,  patients,  healthcare
providers  or  others.  If  we  cannot  successfully  defend  ourselves  against  any  such  claims,  we  may  incur  substantial
liabilities. Regardless of their merit or eventual outcome, product liability claims may result in:

● withdrawal of clinical trial participants;

● termination of clinical trial sites or entire clinical trial programs;

● costs of related litigation;

● substantial monetary awards to patients or other claimants;

● decreased demand for our products and loss of revenues;

● impairment of our business reputation;

● diversion of management and scientific resources from our business operations; and

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● the  inability  to  develop  and  commercialize  our  products  and  product  candidates  or  the  withdrawal  of  our

products from the market.

We have obtained limited product liability insurance coverage. Our insurance coverage may not reimburse us or may
not  be  sufficient  to  reimburse  us  for  any  expenses  or  losses  we  may  suffer.  Moreover,  insurance  coverage  is  becoming
increasingly expensive, and, in the future, we may not be able to maintain insurance coverage at a reasonable cost or in
sufficient amounts to protect us against losses due to product liability. Large judgments have been awarded in class action
lawsuits based on the unanticipated side effects of drug products. A successful product liability claim or series of claims
brought  against  us,  particularly  if  judgments  exceed  our  insurance  coverage,  could  decrease  our  cash  resources  and
adversely affect our business.

Risks Related to Our Intellectual Property

It is difficult and costly to protect our proprietary rights, and we may not be able to ensure their protection. If our patent
position does not adequately protect our products such as Ocaliva and product candidates such as OCA for liver fibrosis
due to NASH, others may compete against us more directly, which could harm our business, possibly materially.

Our commercial success will depend in part on our ability to obtain and maintain patent, trademark and trade secret
protection covering Ocaliva, OCA for liver fibrosis due to NASH, if approved, and our other product candidates, as well as
our ability to successfully defend our intellectual property against third-party challenges. Our ability to stop third parties
from  making,  using,  selling,  offering  to  sell  or  importing  our  products  is  dependent  upon  the  extent  to  which  we  have
regulatory  exclusivity  or  intellectual  property-based  exclusivity  rights  under  valid  and  enforceable  patents  or  other
intellectual property that cover our products. If we fail to obtain and maintain adequate intellectual property protection, we
may  not  be  able  to  prevent  third  parties  from  launching  generic  versions  of  our  products,  from  using  our  proprietary
technologies  or  from  marketing  products  that  are  very  similar  or  identical  to  ours.  For  example,  we  have  received
paragraph IV certification notice letters from several generic drug manufacturers indicating that each such company has
submitted to the FDA an ANDA seeking approval to manufacture and sell a generic version of our 5 mg and 10 mg dosage
strengths  of  Ocaliva  (obeticholic  acid)  for  PBC  prior  to  the  expiration  of  certain  patents  protecting  Ocaliva.  We  have
initiated patent infringement suits against each of these generic drug manufacturers in the United States District Court for
the  District  of  Delaware.  While  we  intend  to  vigorously  defend  and  enforce  our  intellectual  property  rights  protecting
Ocaliva, we can offer no assurance as to when the lawsuits will be decided, or whether the lawsuits will be successful. If a
generic equivalent of Ocaliva is approved and enters the market before the expiration of our patents protecting Ocaliva, our
business may be materially and adversely affected. See Note 19 to our audited consolidated financial statements included
elsewhere in this Annual Report on Form 10-K for more information.

The  patent  positions  of  pharmaceutical  companies  can  be  highly  uncertain  and  involve  complex  legal  and  factual
questions  for  which  important  legal  principles  remain  unresolved.  No  consistent  policy  regarding  the  breadth  of  claims
allowed  in  pharmaceutical  patents  has  emerged  to  date  in  the  United  States  or  in  foreign  jurisdictions,  and  the  legal
standards relating to the patentability, validity and enforceability of pharmaceutical patents are evolving. Changes in either
the  patent  laws  or  in  interpretations  of  patent  laws  in  U.S.  and  foreign  jurisdictions  may  diminish  the  value  of  our
intellectual  property.  Accordingly,  we  cannot  predict  the  breadth  of  claims  that  may  be  enforced  in  the  patents  that  we
currently own or that may issue from the applications we have filed or may file in the future or those that we may license
from third parties. Additionally, our currently pending or future patent applications may not result in issued patents, and
any term extensions or reissues that we seek may not be granted. Further, if any patents we obtain or license are deemed
invalid or unenforceable, it could impact our ability to commercialize or license our technology or we may not be able to
prevent third parties from launching generic versions of our products, or from developing or marketing products that are
similar or identical to ours.

There have been numerous changes to the patent laws that may have a significant impact on our ability to protect our
technology and enforce our intellectual property rights. In September 2011, the America Invents Act was signed into law.
The  final  substantive  provisions  of  the  America  Invents  Act  became  effective  in  March  2013.  The  America  Invents  Act
included a number of significant changes to U.S. patent law that affect the way patent applications are filed, prosecuted and
litigated, including, among other things, changing from a “first to invent” to a “first inventor to file” system and creating
processes, such as Inter Partes Review (“IPR”) and other post-grant review processes, that permit third parties to

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challenge the validity of granted patents before the Patent Trial and Appeal Board of the U.S. Patent and Trademark Office
(the “USPTO”). The IPR process, for example, permits any person to challenge the validity of a patent on the grounds that
it  was  anticipated  or  made  obvious  by  prior  art.  The  America  Invents  Act  and  its  implementation  could  increase  the
uncertainties and costs surrounding the prosecution of our patent applications and the enforcement or defense of our issued
patents,  all  of  which  could  have  a  material  adverse  effect  on  our  business,  financial  condition,  results  of  operations  and
growth prospects.

Others have filed, and in the future, are likely to file, patent applications covering products and technologies that are
similar or competitive to ours, or may be important to our business. We cannot be certain that any patent application owned
by a third party will not have priority over patent applications filed or in-licensed by us, or that we or our licensors will not
be involved in infringement, interference, derivation, opposition, nullity, invalidity or other similar proceedings before U.S.
or non-U.S. patent offices or courts.

The degree to which our patents protect our products may be limited due to a number of factors. For example:

● others may be able to develop and market products that are similar to our products or product candidates but

not covered by the claims of our patents;

● we  might  not  have  been  the  first  to  conceive  of  the  inventions  covered  by  our  patents  or  pending  patent

applications;

● we might not have been the first to file patent applications for these inventions;

● patents that we obtain may not provide us with competitive advantages or exclusivity in a particular product

area or indication or for the length of time we have anticipated; or

● the patents of others may have an adverse effect on our business.

We are the owner of record of numerous issued U.S. and non-U.S. patents and patent applications with claims directed
to  pharmaceutical  compounds,  pharmaceutical  compositions,  formulations,  methods  of  making  these  compounds  and
methods of using these compounds in various indications.

Our issued patents for OCA are expected to expire between 2022 and 2036 if the appropriate maintenance, renewal,
annuity, or other government fees are paid. Without patent protection, including patent protection covering the composition
of  matter,  methods  of  using  and  formulations  of  our  products  and  product  candidates,  our  ability  to  stop  others  from
making, using, selling, offering to sell or importing our products and product candidates may be limited.

Due  to  the  patent  laws  of  a  specific  country  in  which  we  are  seeking  patent  protection,  the  decisions  of  a  patent
examiner in a specific country in which we are seeking patent protection or our own filing strategies, we ultimately may
not  obtain  patent  coverage  for  all  of  our  products  and  product  candidates  for  which  we  have  filed  a  patent  application.
While  we  regularly  pursue  patent  protection  in  the  United  States  and  other  countries  to  obtain  claim  coverage  for  our
inventions, we cannot be certain that such patent rights will be granted or that the scope of any patent granted will prevent
third parties from making, using, selling, offering for sale or importing the same or similar products.

If we do not obtain protection under the Hatch-Waxman Act in the United States (and similar legislation outside of the
United  States)  extending  the  terms  of  our  patents  and/or  providing  data  or  other  exclusivity  for  our  products  and
product candidates, our business may be materially harmed.

Depending upon the timing, duration and specifics of FDA marketing approval of our products, U.S. patents may be
eligible for a limited extension of patent term under the Drug Price Competition and Patent Term Restoration Act of 1984
(the “Hatch-Waxman Act”). The Hatch-Waxman Act permits an extension of patent term for one patent of up to five years
as compensation for patent term lost during product development and the FDA regulatory review process, so long as the
total period of patent term extension does not exceed 14 years from the date of approval. However, an extension may not

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be  granted  because  of,  for  example,  failure  to  apply  within  applicable  deadlines,  failure  to  apply  prior  to  expiration  of
relevant  patents  or  failure  to  satisfy  applicable  requirements.  Moreover,  the  applicable  time  period  or  scope  of  patent
protection afforded could be less than what is requested. If we are unable to obtain patent term extension or the term of any
such  extension  is  less  than  what  we  request,  the  period  during  which  we  will  have  the  right  to  exclusively  market  our
products may be shorter than anticipated, our competitors may obtain approval of competing products following our patent
expiration and our revenue could be reduced, possibly materially.

In October 2020, the USPTO granted to the Company a reissue patent, U.S. Patent No. RE 48,286 (the “‘286 Patent”).
By operation of law, our primary composition of matter patent protecting Ocaliva, U.S. Patent No. 7,138,390 (the “‘390
Patent”), was withdrawn and replaced by the ‘286 Patent, which contains composition of matter claims to OCA. The ‘286
Patent has been substituted in any litigation where the ‘390 Patent was asserted. The ‘286 Patent, like its predecessor the
‘390 Patent, was scheduled to expire in 2022. In light of the U.S. marketing approval of Ocaliva for PBC in May 2016, and
pursuant to the Hatch-Waxman Act, we previously applied for an extension of the patent term for the ‘390 Patent in the
U.S. seeking to extend the term of the ‘390 Patent into 2027. After the ‘286 Patent issued, the application for extension of
patent  term  was  transferred  to  the  ‘286  Patent.  In  November  2020,  the  Company  was  informed  by  the  USPTO  that  its
petition for a five-year patent term extension had been granted. Accordingly, the patent term extension originally intended
to extend the term of the ‘390 Patent into 2027 will extend the term of the ‘286 Patent into 2027. Similarly, in connection
with the conditional approval of Ocaliva for PBC in the European Union, we applied for supplementary patent certification
(“SPC”)  to  extend  the  patent  term  for  the  European  analogue  of  the  ‘390  Patent  (now  the  ‘286  Patent)  in  most  of  the
European  Union  into  2027.  To  date,  we  have  received  grants  of  SPC  in  Austria,  Cyprus,  Denmark,  Finland,  France,
Germany,  Greece,  Ireland,  Italy,  Norway,  Portugal,  Spain  and  Sweden.  We  have  also  taken  similar  actions  in  other
jurisdictions  and  countries  where  regulations  providing  for  patent  term  extension  exist.  The  issued  patents  for  OCA  are
expected to expire between 2022 and 2036 if the appropriate maintenance, renewal, annuity, or other government fees are
paid. The substitution in the U.S. of the ‘286 Patent for the ‘390 Patent has no effect on foreign patent rights.

We  may  incur  substantial  costs  as  a  result  of  litigation  or  other  proceedings  relating  to  patent  and  other  intellectual
property rights, and such litigation may divert the attention of our management and scientific personnel and adversely
affect our development and commercialization efforts.

If we choose to file patent infringement lawsuits or engage in other adversarial proceedings to stop another party from
making,  using,  selling,  offering  for  sale  or  importing  the  inventions  claimed  in  any  of  our  patents,  that  individual  or
company alleged to be infringing has the right to ask the court or adjudicating body to rule that such patents are invalid, not
infringed or should not be enforced against that third party. These lawsuits and proceedings are expensive, consume time
and resources and divert the attention of management and scientific personnel even if we are successful in defending our
rights.  In  addition,  there  is  a  risk  that  such  court  or  adjudicating  body  will  decide  that  such  patents  are  invalid,
unenforceable  or  not  infringed,  and  that  we  do  not  have  the  right  to  stop  the  other  party  from  making,  using,  selling,
offering for sale or importing the inventions. For example, we have received paragraph IV certification notice letters from
several  generic  drug  manufacturers  indicating  that  each  such  company  has  submitted  to  the  FDA  an  ANDA  seeking
approval to manufacture and sell a generic version of our 5 mg and 10 mg dosage strengths of Ocaliva (obeticholic acid)
for PBC prior to the expiration of certain patents protecting Ocaliva. We have initiated patent infringement suits against
each of these generic drug manufacturers in the United States District Court for the District of Delaware. Such lawsuits
may  be  expensive  and  divert  our  management’s  time  and  attention.  In  addition,  to  the  extent  such  lawsuits  are  not
successful,  and  a  generic  equivalent  of  Ocaliva  is  approved  and  enters  the  market  before  the  expiration  of  our  patents
protecting  Ocaliva,  our  business  may  be  materially  and  adversely  affected.  See  Note  19  to  our  audited  consolidated
financial statements included elsewhere in this Annual Report on Form 10-K for more information.

Over the past 20 years, the U.S. Supreme Court and the U.S. Congress have modified certain examination procedures
utilized  by  the  USPTO  in  granting  patents,  which  has  raised  the  standard  of  patentability  for  some  types  of  inventions.
Such modifications may reduce the likelihood that we will be able to obtain patent protection and increase the likelihood of
challenges to our patents or the patents we license.

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We may infringe the intellectual property rights of others, which may prevent or delay our product development efforts
and/or delay, halt or increase the costs of our commercialization efforts.

Our success will depend in part on our ability to operate without infringing the proprietary rights of third parties. We
cannot guarantee that the use, manufacture, sale, offer for sale or importation of our products will not infringe third-party
patents.  Furthermore,  a  third  party  may  claim  that  we  or  our  manufacturing  or  commercialization  partners  are  using
inventions covered by the third party’s patent rights and may go to court to stop us from engaging in our normal operations
and  activities,  including  making  or  selling  our  products  and  product  candidates.  The  defense  of  these  lawsuits  is  often
costly and could affect our results of operations and divert the attention of our management and scientific personnel. There
is also a risk that a court could decide that we or our manufacturing or commercialization partners are infringing the third
party’s patents and order us or our partners to stop the activities covered by the patents. In that event, we or our partners
may  be  required  to  halt  or  delay  commercialization  or  development  of  the  relevant  product  or  product  candidate.  In
addition, there is a risk that a court could order us or our partners to pay the other party damages for having violated the
other party’s patents, and we may be subject to indemnification obligations with respect to any such payments made by our
partners. There is a vast array of patents and patent applications that claim various pharmaceutical inventions and because
the scope of a patent’s claims is subject to interpretation by the courts, it is not always clear to industry participants which
patents  cover  various  types  of  products,  product  candidates  or  methods  of  use.  In  addition,  interpretation  of  a  patent’s
claims can vary from court to court.

If we are sued for patent infringement, we would need to demonstrate that the relevant patent is not enforceable or that
our products, product candidates or methods either do not infringe the patent claims of the relevant patent or that the patent
claims are invalid. Proving invalidity, non-infringement and/or unenforceability is difficult, and we may not be successful.
For example, in the United States, proving invalidity requires a showing of clear and convincing evidence to overcome the
presumption of validity enjoyed by issued patents. Even if we are successful in such proceedings, we may incur substantial
costs and divert our management’s time and attention, which could have a material adverse effect on our business. If we are
unable to avoid infringing the patent rights of others, we may be required to seek a license, which may not be available,
defend  an  infringement  action  or  challenge  the  validity  of  the  patents  in  court.  Patent  litigation  is  costly  and  time
consuming. We may not have sufficient resources to bring these actions to a successful conclusion. In addition, if we fail to
obtain a license, develop or obtain non-infringing technology or defend an infringement action successfully, we may incur
substantial  monetary  damages,  encounter  significant  delays  in  the  commercialization  of  our  products  and  product
candidates and be precluded from manufacturing or selling our products and product candidates.

We cannot be certain that others have not filed patent applications for technology covered by our pending applications,

or that we were the first to invent or file with respect to a technology, because:

● some patent applications in the United States may be unpublished or otherwise maintained in secrecy until

the patents are issued;

● patent applications in the United States are typically not published until 18 months after the priority date; and

● publications in the scientific literature often lag behind actual discoveries.

Our competitors may have filed, and may in the future file, patent applications covering technology similar to ours.
Any such patent application may have priority over our patent applications, which could further require us to obtain rights
to issued patents covering such technologies. If another party has filed a U.S. patent application on inventions similar to
ours,  we  may  have  to  participate  in  an  interference,  derivation  or  other  similar  proceeding  declared  by  the  USPTO  to
determine priority of invention in the United States. The costs of these proceedings could be substantial, and it is possible
that  such  efforts  would  be  unsuccessful,  resulting  in  a  loss  of  our  U.S.  patent  position  with  respect  to  such  inventions.
Other countries have similar laws that permit secrecy of patent applications, and such patent applications may be entitled to
priority over our applications in such jurisdictions.

Some of our competitors may be able to sustain the costs of complex patent litigation more effectively than we can
because they have substantially greater financial and other resources. In addition, uncertainties resulting from the initiation

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and continuation of any such litigation could have a material adverse effect on the market price of our securities and our
ability to raise the funds necessary to continue our operations.

Obtaining  and  maintaining  our  patent  protection  depends  on  compliance  with  various  procedural,  document
submission, fee payment and other requirements imposed by governmental patent agencies, and our patent protection
could be reduced or eliminated as a result of non-compliance with these requirements.

Periodic maintenance fees, renewal fees, annuity fees and various other governmental fees on our patents and patent
applications  are  required  to  be  paid  to  the  USPTO  and  foreign  patent  offices  in  several  stages  over  the  lifetime  of  such
patents and patent applications. In addition, the USPTO and foreign patent agencies require compliance with a number of
procedural,  documentary,  fee  payment  and  other  similar  provisions  during  the  patent  application  process.  We  have
implemented  systems  and  engaged  reputable  third-party  service  providers  to  help  ensure  that  we  comply  with  such
requirements  on  a  timely  basis,  but  inadvertent  lapses  may  occur  and  there  are  situations  in  which  noncompliance  can
result in abandonment or lapse of the relevant patent or patent application, resulting in partial or complete loss of patent
rights in the relevant jurisdiction. Any such event may impair our competitive position in the relevant jurisdiction and have
a material adverse effect on our financial condition or results of operations.

We  may  be  subject  to  claims  that  our  employees  have  wrongfully  used  or  disclosed  alleged  trade  secrets  or  other
proprietary information of their former employers. In addition, if we are not able to adequately prevent disclosure of our
trade secrets and other proprietary information, the value of our technology, products and product candidates could be
significantly diminished.

As  is  common  in  the  biotechnology  and  pharmaceutical  industries,  we  employ  individuals  who  were  previously
employed  at  other  biotechnology  or  pharmaceutical  companies,  including  our  competitors  or  potential  competitors.  We
may be subject to claims that these employees, or we, have inadvertently or otherwise used or disclosed trade secrets or
other proprietary information of their former employers. Litigation may be necessary to defend against these claims, which
could result in substantial costs and be a distraction to our management even if we are successful.

We  may  rely  on  trade  secrets  to  protect  our  proprietary  technologies,  especially  where  we  do  not  believe  patent
protection  is  appropriate  or  obtainable.  However,  trade  secrets  are  difficult  to  protect,  and  may  not  prevent  others  from
independently and lawfully developing similar or identical products that circumvent our intellectual property. We rely in
part on confidentiality agreements with our employees, consultants, outside scientific collaborators, sponsored researchers
and  other  advisors  to  protect  our  trade  secrets  and  other  proprietary  information.  These  agreements  may  not  effectively
prevent  disclosure  of  proprietary  information  and  may  not  provide  an  adequate  remedy  in  the  event  of  unauthorized
disclosure of confidential information.

Third  parties,  including  competitors  of  ours,  may  also  independently  discover  our  trade  secrets  or  other  proprietary
information. In addition, we may be required under U.S. or foreign transparency initiatives or other regulations to publicly
disclose  or  otherwise  make  available  certain  information  that  we  consider  to  be  proprietary,  including  pre-clinical  and
clinical research data. Enforcing a claim that a third party illegally obtained and is using any of our trade secrets or other
proprietary information is expensive and time consuming, and the outcome is unpredictable. In addition, courts outside of
the United States are sometimes reluctant to protect trade secrets. Costly and time-consuming litigation could be necessary
to enforce and determine the scope of our proprietary rights, and failure to obtain or maintain protection of our trade secrets
and other proprietary information could adversely affect our competitive business position.

We  have  not  yet  registered  all  of  our  trademarks  and  failure  to  secure  such  registrations  could  adversely  affect  our
business.

We have numerous trademark and service mark registrations and pending trademark and service mark applications in

the United States and abroad.

Our trademark applications may not be allowed for registration and our registered trademarks may not be maintained
or enforced. During prosecution of applications for trademark registration, we may receive rejections or refusals. Although
we are given an opportunity to respond, we may be unable to overcome such rejections. In addition, the USPTO and

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comparable  agencies  in  many  other  jurisdictions  provide  third  parties  with  an  opportunity  to  oppose  pending  trademark
applications and to seek to cancel registered trademarks. Opposition or cancellation proceedings have been filed and may
in the future be filed against certain of our trademarks, and our trademarks may not survive such proceedings. If we do not
secure registrations for our trademarks, we may encounter more difficulty in enforcing them against third parties than we
otherwise would.

Trademark protection varies in accordance with local laws. Trademarks remain in force in some countries as long as
the trademark is used and in other countries as long as the trademark is registered. Trademark registrations generally are for
fixed but renewable terms. We cannot provide any assurances that any trademarks or service marks will be sufficient to
prevent competitors from adopting similar names. The adoption of similar names by competitors could impede our ability
to build brand identity and may lead to customer confusion, which could adversely affect our sales or profitability.

Risks Related to Our Indebtedness

Servicing our debt will require significant amounts of cash, and we may not have sufficient cash flow from our business
to effectively service our debt.

Our  ability  to  make  scheduled  payments  of  the  principal  of,  to  pay  interest  on  or  to  refinance  the  $460.0  million
aggregate  principal  amount  of  2023  Convertible  Notes  that  we  issued  in  July  2016  and/or  the  $230.0  million  aggregate
principal amount of 2026 Convertible Notes that we issued in May 2019 or any other indebtedness we or our subsidiaries
may incur in the future depends on our future performance, which is subject to economic, financial, competitive and other
factors beyond our control. Our business may not generate cash flow from operations in the future sufficient to service our
debt, including the Convertible Notes. If we are unable to generate cash flow, we may be required to adopt one or more
alternatives,  such  as  selling  assets,  restructuring  debt  or  obtaining  additional  equity  capital  on  terms  that  may  be
unfavorable to us or highly dilutive. Our ability to refinance our indebtedness will depend on the capital markets and our
financial  condition  at  the  time  we  seek  to  refinance  such  indebtedness.  We  may  not  be  able  to  engage  in  any  of  these
activities or engage in these activities on desirable terms, which could result in a default on our debt obligations.

We  may  incur  substantially  more  debt  or  take  other  actions  that  would  affect  our  ability  to  pay  the  principal  of  and
interest on our debt.

We and our subsidiaries may be able to incur substantial additional debt in the future, some of which may be secured
debt.  We  and  our  subsidiaries  are  not  restricted  under  the  terms  of  the  indentures  governing  the  Convertible  Notes  or
otherwise from incurring additional debt, securing existing or future debt, recapitalizing our debt or taking other actions
that could have the effect of diminishing our ability to service our debt when due.

The accounting method for convertible debt securities that may be settled in cash, such as the Convertible Notes, could
have a material effect on our reported financial results.

Under Accounting Standards Codification Subtopic 470-20, “Debt with Conversion and Other Options” (“ASC 470-
20”), an entity must separately account for the liability and equity components of convertible debt instruments (such as the
Convertible Notes) that may be settled entirely or partially in cash upon conversion in a manner that reflects the issuer’s
economic interest cost. The effect of ASC 470-20 on the accounting for the Convertible Notes is that the equity component
is  required  to  be  included  in  the  additional  paid-in  capital  section  of  stockholders’  equity  on  our  consolidated  balance
sheets, and the value of the equity component is treated as original issue discount for purposes of accounting for the debt
component of the Convertible Notes. As a result, we are required to record a greater amount of non-cash interest expense in
current periods presented as a result of the amortization of the discounted carrying value of the Convertible Notes to their
face  amount  over  the  term  of  the  Convertible  Notes.  Because  ASC  470-20  requires  interest  to  include  both  the  current
period’s amortization of the debt discount and the instrument’s coupon interest, we report lower net income in our financial
results, which could adversely affect the market price of our common stock and the market price of the Convertible Notes.

In  addition,  under  certain  circumstances,  convertible  debt  instruments  (such  as  the  Convertible  Notes)  that  may  be
settled entirely or partly in cash are currently accounted for utilizing the treasury stock method, the effect of which is that
the shares issuable upon conversion of the Convertible Notes will not be included in the calculation of diluted earnings per

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share except to the extent that the conversion value of the notes exceeds their principal amount. Under the treasury stock
method,  for  diluted  earnings  per  share  purposes,  the  transaction  is  accounted  for  as  if  the  number  of  shares  of  common
stock that would be necessary to settle such excess, if we elected to settle such excess in shares, are issued. We cannot be
sure  that  the  accounting  standards  in  the  future  will  continue  to  permit  the  use  of  the  treasury  stock  method.  If  we  are
unable to use the treasury stock method in accounting for the shares issuable upon conversion of the Convertible Notes,
then our diluted earnings per share would be adversely affected.

Risks Related to Ownership of Our Common Stock

Ownership in our common stock is highly concentrated and your ability to influence corporate matters may be limited
as a result.

Our executive officers, directors and stockholders who own more than 5% of our outstanding common stock together
beneficially own a significant percentage of our common stock based on reports filed with the SEC. If these stockholders
were  to  choose  to  act  together,  they  would  be  able  to  significantly  influence  matters  submitted  to  our  stockholders  for
approval, including the election of directors and approval of any merger, consolidation, sale of all or substantially all of our
assets or other business combination or reorganization, as well as our management and affairs. This concentration of voting
power  could  delay  or  prevent  an  acquisition  of  us  on  terms  that  other  securityholders  may  desire.  The  interests  of  this
group of stockholders may not always coincide with your interests or the interests of other securityholders and they may
act  in  a  manner  that  advances  their  best  interests  and  not  necessarily  those  of  other  securityholders,  including  seeking  a
premium value for their common stock, and might affect the market price of our common stock and the Convertible Notes.

We have a significant stockholder, which will limit your ability to influence corporate matters, may give rise to conflicts
of interest and could result in future substantial sales of shares of our common stock into the market.

Genextra  S.p.A.  (“Genextra”)  is  one  of  our  largest  stockholders  and  owns  a  significant  minority  percentage  of  our
outstanding common stock. Accordingly, Genextra exerts and will continue to exert significant influence over us and any
action requiring the approval of the holders of our common stock, including the election of directors and amendments to
our  organizational  documents,  such  as  increases  in  our  authorized  shares  of  common  stock  and  approval  of  significant
corporate transactions. This concentration of voting power makes it less likely that other holders of common stock will be
able to affect the way we are managed and could delay or prevent an acquisition of us on terms that other securityholders
may desire.

Furthermore,  the  interests  of  Genextra  may  not  always  coincide  with  the  interests  of  other  securityholders,  and
Genextra may act in a manner that advances its best interests and not necessarily those of other securityholders, including
seeking a premium value for its common stock, and might affect the market price of our common stock and the Convertible
Notes. Our board of directors, which consists of eleven directors, including one associated with Genextra, has the power to
set the number of directors on our board from time to time.

Genextra  also  may  sell  shares  of  our  common  stock  into  the  market  from  time  to  time,  and  we  cannot  predict  the

effect, if any, that future sales by Genextra may have on the market price of our common stock or the Convertible Notes.

An active trading market in our common stock may not be maintained.

The  trading  market  in  our  common  stock  has  been  extremely  volatile.  The  quotation  of  our  common  stock  on  the
Nasdaq Global Select Market does not assure that a meaningful, consistent and liquid trading market will exist. We cannot
predict whether an active market for our common stock will be maintained in the future. An absence of an active trading
market  could  adversely  affect  your  ability  to  sell  our  common  stock  at  current  market  prices  in  short  time  periods,  or
possibly at all. Additionally, market visibility for our common stock may be limited and such lack of visibility may have a
depressive effect on the market price for our common stock.

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We have previously been, and are currently, subject to securities class action litigation and may be subject to similar or
other litigation in the future. Such matters can be expensive, time-consuming and have a material adverse effect on our
business, results of operations and financial condition.

We have previously been subject to securities class action lawsuits. In February 2014, two purported securities class
actions were filed against us and certain of our officers, which were eventually consolidated. In May 2016, the defendants
reached  an  agreement  with  the  lead  plaintiff  to  seek  court  approval  of  a  proposed  resolution  and  the  settlement  was
ultimately granted final approval by the court in September 2016. While the final judgment and order of the court included
a dismissal of the action with prejudice against all defendants and the defendants did not admit any liability as part of the
settlement, the total payment aggregated to $55.0 million, of which $10.0 million was paid by our insurers.

In September 2017, a lawsuit and, in January 2018, a follow-on lawsuit, were filed alleging that we and certain of our
officers  made  material  misrepresentations  and/or  omissions  of  material  fact  regarding  Ocaliva  dosing,  use  and
pharmacovigilance-related  matters,  as  well  as  our  operations,  financial  performance  and  prospects.  The  plaintiffs  seek
unspecified monetary damages on behalf of the putative class, an award of costs and expenses, including attorney’s fees,
and rescissory damages.

While  we  believe  that  we  have  a  number  of  valid  defenses  to  the  claims  described  above  and  intend  to  vigorously
defend ourselves, the matters are in the early stages of litigation and no assessment can be made as to the likely outcome of
the matters or whether they will be material to us.

Additionally, in November 2020, a lawsuit and, in December 2020 and February 2021, follow-on lawsuits, were filed
alleging that we and certain of our officers made material misrepresentations and/or omissions of material fact during the
period from September 28, 2019 to October 7, 2020 relating to our NDA for OCA for the treatment of liver fibrosis due to
NASH and the use of Ocaliva in patients with PBC, as well as our operations, financial performance and prospects. The
plaintiff seeks unspecified monetary damages on behalf of the putative class, and an award of costs and expenses, including
attorney’s fees.

We  may  be  subject  to  additional  suits  or  proceedings  brought  in  the  future  and,  as  has  been  the  case  with  many
companies  in  our  industry,  we  may  from  time  to  time  receive  inquiries  and  subpoenas  and  other  types  of  information
requests  from  government  authorities  and  others.  While  the  ultimate  outcome  of  any  such  investigations,  inquiries,
information requests and legal proceedings is difficult to predict, adverse resolutions or settlements of those matters may
result in, among other things, modification of our business practices, product recalls, significant costs, payments, damages
or fines or other administrative, civil or criminal remedies, liabilities or penalties, which may have a material adverse effect
on our business, results of operations and financial condition. In addition, monitoring and defending against legal actions,
whether  or  not  meritorious,  and  responding  to  investigations,  inquiries  and  information  requests  is  expensive,  time-
consuming for our management and detracts from our ability to fully focus our internal resources on our business activities,
and  we  cannot  predict  how  long  it  may  take  to  resolve  such  matters.  Although  we  may  receive  insurance  coverage  for
certain adversarial proceedings, coverage could be denied or prove to be insufficient. It is possible that we could, in the
future, incur a judgment or enter into settlement of claims for monetary damages. A decision adverse to our interests could
result in the payment of substantial damages and could have a material adverse effect on our business, results of operations
and financial condition.

Our stock price has been and may in the future be volatile, which could cause holders of our common stock to incur
substantial losses.

The market price of our common stock has been, and is likely to continue to be, highly volatile and could be subject to
wide fluctuations in response to various factors, some of which are beyond our control. Since our initial public offering in
October 2012, the price of our common stock on the Nasdaq Global Select Market has ranged from $17.96 per share to
$497.00 per share. In addition to the other factors discussed in this “Risk Factors” section and elsewhere in this Annual
Report on Form 10-K, the factors that may result in wide fluctuations in the price of our common stock include any:

● delay, failure or receipt of regulatory approval for our product candidates, including OCA for liver fibrosis

due to NASH;

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● delay,  failure  or  receipt  of  additional  marketing  authorizations  for  Ocaliva  or  our  product  candidates,

including OCA for liver fibrosis due to NASH, in our target markets;

● failure to successfully commercialize our approved products in the United States, Europe and our other target
markets, or our inability to maintain regulatory approval for Ocaliva or our other approved products in such
markets;

● clinical  trial  failure,  including  any  such  failure  resulting  from  issues,  delays  or  difficulties  in  identifying
patients, enrolling patients, treating patients, retaining patients, meeting specific endpoints in the jurisdictions
in which we intend to seek approval or completing and timely reporting the results of our clinical trials, such
as our NASH and PBC trials;

● the  effects  of  COVID-19  and  related  government-imposed  shelter-in-place  mandates,  restrictions  on  travel

and in-person interactions, business closures and disruptions and other public health safety measures;

● inability to obtain additional funding;

● delay in filing an investigational new drug application, NDA, MAA or comparable submission for any of our
product  candidates,  and  any  adverse  development  or  perceived  adverse  development  with  respect  to  the
regulatory review of any such submission;

● potential  side  effects  associated  with  Ocaliva  for  PBC,  OCA  for  liver  fibrosis  due  to  NASH  or  our  other

product candidates;

● inability to obtain adequate product supply of Ocaliva, OCA for liver fibrosis due to NASH or any of our

other product candidates or the inability to do so at acceptable prices;

● results of clinical trials of our competitors’ products and product candidates;

● regulatory  or  advisory  committee  actions  or  recommendations  with  respect  to  our  products  or  product
candidates,  including  Ocaliva  or  OCA  for  liver  fibrosis  due  to  NASH,  or  our  competitors’  products  or
product candidates;

● changes in laws or regulations applicable to our products or product candidates;

● failure to meet or exceed financial projections or guidance we may provide to the public;

● failure to meet or exceed the estimates and projections of the investment community;

● actual or anticipated fluctuations in our financial condition and operating results;

● actual or anticipated changes in our growth rate relative to our competitors;

● actual or anticipated fluctuations in our competitors’ operating results or changes in their growth rate;

● competition from existing products or new products that may emerge;

● announcements  by  us,  our  collaborators  or  our  competitors  of  significant  acquisitions,  strategic

collaborations, joint ventures, collaborations or capital commitments;

● issuance of new or updated research or reports by securities analysts;

● fluctuations in the valuation of companies perceived by investors to be comparable to us;

● share price and volume fluctuations attributable to inconsistent trading volume levels of our shares;

● additions or departures of key management or scientific personnel;

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● disputes  or  other  developments  related  to  proprietary  rights,  including  patents,  litigation  matters  and  our

ability to obtain patent protection for our technologies;

● announcement or expectation of additional financing efforts;

● disputes,  governmental  inquiries  or  investigations,  legal  proceedings  or  litigation,  including  any  securities,

intellectual property, employment, product liability or other litigation;

● sales of our common stock by us, our insiders or our other stockholders;

● failure  to  adopt  appropriate  information  security  systems,  including  any  systems  that  may  be  required  to
support  our  growing  and  changing  business  requirements,  or  prevent  system  failures,  data  breaches  or
violations of data protection laws;

● market conditions for biopharmaceutical stocks in general; and

● general economic, industry, market and political conditions

Any of these factors could also affect the trading price of the Convertible Notes.

Furthermore,  stock  markets  in  general  and  the  market  for  biotechnology  companies  in  particular  have  experienced
extreme  price  and  volume  fluctuations  that  have  affected  and  continue  to  affect  the  market  prices  of  securities  of  many
companies.  These  fluctuations  often  have  been  unrelated  or  disproportionate  to  the  operating  performance  of  those
companies. A number of factors, including global health emergencies (e.g., COVID-19), general economic, political and
market conditions, recessions, interest rate changes or international currency fluctuations may negatively impact the market
price  of  our  securities,  regardless  of  our  actual  operating  performance.  In  the  past,  companies  that  have  experienced
volatility in the market price of their stock have been subject to securities class action litigation. We have been in the past,
and  are  currently  subject  to  this  type  of  litigation,  which  could  result  in  substantial  costs  and  divert  our  management’s
attention from other business concerns, which could seriously harm our business. As a result of this volatility, you could
incur substantial losses.

If  our  stockholders  sell  substantial  amounts  of  our  common  stock,  the  market  price  of  our  common  stock  or  the
Convertible Notes may decline even if our business is doing well.

A significant number of shares of our common stock are held by a small number of stockholders, including Genextra.
Sales  of  a  significant  number  of  shares  of  our  common  stock,  or  the  expectation  that  such  sales  may  occur,  could
significantly  reduce  the  market  price  of  our  common  stock  or  the  Convertible  Notes.  These  sales,  or  the  possibility  that
these sales may occur, also might make it more difficult for us to sell equity securities in the future at a time and price that
we deem appropriate. We have also registered the offer and sale of the shares of common stock that we may issue under
our equity compensation plans, including upon the exercise of stock options. These shares may be freely sold in the public
market upon issuance.

Additionally, sales of our common stock by our executive officers or directors, even when done during an open trading
window  under  our  policies  with  respect  to  insider  sales  or  done  under  a  trading  plan  adopted  in  accordance  with  the
guidelines set forth by Rule 10b5-1, may adversely impact the market price of our common stock or the Convertible Notes.
Although we do not expect that the relatively small volume of such sales would itself significantly impact the market price
of our common stock or the Convertible Notes, the market could react negatively to the announcement of such sales, which
could in turn affect the market price of our common stock and the Convertible Notes.

You may experience future dilution as a result of future equity offerings or strategic transactions.

We  may  in  the  future  raise  funds  through  the  issuance  and  sale  of  additional  shares  of  our  common  stock  or  other
securities  convertible  into  or  exchangeable  for  our  common  stock.  For  example,  in  May  2019,  we  issued  and  sold  an
aggregate of 2,879,760 shares of common stock and $230.0 million aggregate principal amount of the 2026 Convertible
Notes, in April 2018, we issued and sold an aggregate of 4,257,813 shares of common stock and in July 2016, we issued

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and  sold  $460.0  million  aggregate  principal  amount  of  the  2023  Convertible  Notes.  Conversions  of  the  Convertible
Notes  will  dilute  the  ownership  interests  of  existing  shareholders  to  the  extent  that  we  elect  to  deliver  shares  of  our
common  stock  (or  a  combination  of  cash  and  shares  of  our  common  stock)  in  connection  therewith.  In  addition,  the
existence  of  the  Convertible  Notes  may  encourage  short  selling  by  market  participants  because  the  conversion  of  the
Convertible Notes could depress the price of our common stock. We may also issue shares of common stock, stock options,
restricted  stock,  restricted  stock  units  or  other  stock-based  awards  under  our  existing  or  future  equity  incentive  plans  or
other employee or director compensation plans. The issuance of additional shares of common stock (including pursuant to
conversions of the Convertible Notes) or other securities convertible into or exchangeable for our common stock, or the
perception  that  such  issuances  may  occur,  may  materially  and  adversely  affect  the  price  of  our  common  stock  and  the
Convertible Notes.

Anti-takeover  provisions  in  our  restated  certificate  of  incorporation  and  our  restated  bylaws,  as  well  as  provisions  of
Delaware law and certain provisions of the Convertible Notes, might discourage, delay or prevent a change in control of
our  company  or  changes  in  our  management  and,  therefore,  depress  the  market  price  of  our  common  stock  or  the
Convertible Notes.

Provisions in our restated certificate of incorporation and restated bylaws, as well as provisions of Delaware law, may
discourage, delay or prevent a merger, acquisition or other change in control that our securityholders consider favorable,
including transactions in which securityholders might otherwise receive a premium for their securities. These provisions
may  also  prevent  or  frustrate  attempts  by  our  stockholders  to  replace  or  remove  our  management.  Our  corporate
governance documents include provisions:

● authorizing the issuance of “blank check” convertible preferred stock, the terms of which may be established

and shares of which may be issued without stockholder approval;

● prohibiting stockholder action by written consent, thereby requiring all stockholder actions to be taken at a
meeting  of  our  stockholders,  to  the  extent  that  no  stockholder,  together  with  its  affiliates,  holds  more  than
50% of our voting stock;

● eliminating the ability of stockholders to call a special meeting of stockholders;

● permitting  our  board  of  directors  to  accelerate  the  vesting  of  outstanding  equity  awards  upon  certain

transactions that result in a change of control; and

● establishing  advance  notice  requirements  for  nominations  for  election  to  the  board  of  directors  or  for

proposing matters that can be acted upon at stockholder meetings.

In  addition,  as  a  Delaware  corporation,  we  are  subject  to  provisions  of  Delaware  law,  including  Section  203  of  the
Delaware  General  Corporation  Law  (the  “DGCL”),  which  prevents  some  stockholders  holding  more  than  15%  of  our
outstanding common stock from engaging in certain business combinations without approval of the holders of substantially
all  of  our  outstanding  common  stock.  Any  provision  of  our  restated  certificate  of  incorporation  or  restated  bylaws  or
Delaware  law  that  has  the  effect  of  delaying  or  deterring  a  change  in  control  could  limit  the  opportunity  for  our
securityholders to receive a premium for their securities, and could also affect the price that some investors are willing to
pay for our common stock or the Convertible Notes.

Certain provisions of the Convertible Notes could also make it more difficult or more expensive for a third party to
acquire  us.  For  example,  if  an  acquisition  event  constitutes  a  “fundamental  change”  under  the  terms  of  the  Convertible
Notes,  holders  of  the  Convertible  Notes  will  have  the  right  to  require  us  to  purchase  their  Convertible  Notes  for  cash.
Similarly, if an acquisition event constitutes a “make-whole fundamental change” under the terms of the Convertible Notes,
we  may  be  required  to  increase  the  conversion  rate  for  holders  who  convert  their  Convertible  Notes  in  connection  with
such make-whole fundamental change.

The existence of the foregoing provisions and anti-takeover measures may also frustrate or prevent any attempts by
our stockholders to replace or remove our current management or members of our board of directors and could limit the
price that investors might be willing to pay in the future for shares of our common stock or the Convertible Notes. They

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could also deter potential acquirers of our company, thereby reducing the likelihood that our securityholders could receive
a premium for their securities in an acquisition.

Claims  for  indemnification  by  our  directors  and  officers  may  reduce  our  available  funds  to  satisfy  successful
stockholder claims against us and may reduce the amount of money available to us.

As  permitted  by  Section  102(b)(7)  of  the  DGCL,  our  restated  certificate  of  incorporation  limits  the  liability  of  our
directors  to  the  fullest  extent  permitted  by  law.  In  addition,  as  permitted  by  Section  145  of  the  DGCL,  our  restated
certificate  of  incorporation  and  restated  bylaws  provide  that  we  shall  indemnify,  to  the  fullest  extent  authorized  by  the
DGCL,  each  person  who  is  involved  in  any  litigation  or  other  proceeding  because  such  person  is  or  was  a  director  or
officer of our company, or is or was serving as an officer or director of another entity at our request, against all expense,
loss or liability reasonably incurred or suffered in connection therewith. Our restated certificate of incorporation provides
that the right to indemnification includes the right to be paid expenses incurred in defending any proceeding in advance of
its final disposition, subject to certain conditions. The rights conferred in the restated certificate of incorporation and the
restated  bylaws  are  not  exclusive,  and  we  are  authorized  to  enter  into  indemnification  agreements  with  our  directors,
officers, employees and agents and to obtain insurance to indemnify such persons.

The above limitations on liability and our indemnification obligations limit the personal liability of our directors and
officers for monetary damages for breach of their fiduciary duty by shifting the burden of such losses and expenses to us.
Although we carry directors’ and officers’ liability insurance, certain liabilities or expenses covered by our indemnification
obligations may not be covered by such insurance or the coverage limitation amounts may be exceeded. As a result, we
may need to use a significant amount of our funds to satisfy our indemnification obligations, which could severely harm
our  business  and  financial  condition  and  limit  the  funds  available  to  securityholders  who  may  choose  to  bring  a  claim
against our company.

We do not intend to pay dividends in the foreseeable future.

We do not anticipate paying cash dividends in the future. As a result, only appreciation of the price of shares of our
common  stock  will  provide  a  return  to  stockholders,  which  may  not  occur.  Investors  seeking  cash  dividends  should  not
invest in our common stock. You may not realize any return on your investment in our common stock and may lose some
or all of your investment.

Our ability to use our net operating loss carryforwards and certain other tax attributes may be limited.

We  have  significant  net  operating  loss  carryforwards  (“NOLs”)  for  U.S.  Federal,  state  and  foreign  income  tax
purposes. The enactment of the Tax Cuts and Jobs Act enacted in 2017 (the “TCJA”) modified the ability of companies to
utilize U.S. Federal NOLs arising in tax years beginning on or after January 1, 2018, by providing that such NOLs may be
carried-forward indefinitely and used to offset up to 80 percent of taxable income in any given future year. Existing NOLs
that arose in tax years beginning prior to January 1, 2018, were not affected by the TCJA and are generally eligible to be
carried-forward  for  up  to  20  years  and  used  to  fully  offset  taxable  income  in  future  years.  If  not  utilized,  our  pre-2018
NOLs will expire for U.S. Federal income tax purposes between 2024 and 2037. We also have certain state and foreign
NOLs in varying amounts depending on the different state and foreign tax laws.

In  addition,  our  ability  to  utilize  our  NOLs  may  be  limited  under  Section  382  of  the  Internal  Revenue  Code  or
applicable  state  and  foreign  tax  law.  The  Section  382  limitations  apply  if  an  “ownership  change”  occurs.  Generally,  an
ownership change occurs when certain shareholders increase their aggregate ownership by more than 50 percentage points
over their lowest ownership percentage in a testing period (typically three years). We have evaluated whether one or more
ownership changes under Section 382 have occurred since our inception and have determined that there have been at least
two  such  changes.  Although  we  believe  that  these  ownership  changes  have  not  resulted  in  material  limitations  on  our
ability to use these NOLs, our ability to utilize these NOLs may be limited due to future ownership changes or for other
reasons.  As  a  result,  we  may  not  be  able  to  take  full  advantage  of  our  NOL  carryforwards  for  U.S.  Federal,  state,  and
foreign income tax purposes.

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General Risk Factors

We may use our limited financial and human resources to pursue a particular research program or product candidate
that is ultimately unsuccessful or less successful than other programs or product candidates that we may have forgone
or delayed.

Because  we  have  limited  resources,  we  may  forego  or  delay  the  development  of  certain  programs  or  product
candidates that later prove to have greater commercial potential than the programs or product candidates that we do pursue.
Our  resource  allocation  decisions  may  cause  us  to  fail  to  capitalize  on  viable  commercial  products  or  profitable  market
opportunities.  Our  spending  on  current  and  future  research  and  development  programs  for  product  candidates  may  not
yield any commercially viable products. If we fail to accurately evaluate the commercial potential or target market for a
particular product candidate, we may relinquish valuable rights to that product candidate through strategic collaboration,
licensing or other arrangements or we may allocate our limited internal resources to that product candidate when it would
have been more advantageous to enter into such an arrangement. Any such failure could have a material adverse effect on
our business, financial condition or results of operations.

If we engage in a licensing transaction, acquisition, reorganization or business combination, we will face a variety of
risks that could adversely affect our business operations and our securityholders.

From time to time, we have considered, and we will continue to consider in the future, strategic business initiatives
intended to further the expansion and development of our business. These initiatives may include in-licensing or acquiring
products, technologies or businesses, entering into a business combination with another company or otherwise partnering
with another company. If we pursue such a strategy, we could, among other things:

● issue equity securities that would dilute our current stockholders’ ownership;

● incur substantial debt that may place strains on our operations;

● be  required  to  dedicate  substantial  operational,  financial  and  management  resources  to  integrate  new

products, technologies or businesses;

● assume substantial actual or contingent liabilities;

● impair  our  ability  to  make  payments  of  interest  and  principal  on  our  outstanding  debt,  including  the

Convertible Notes;

● reprioritize our development programs or cease development and commercialization activities with respect to

certain of our product candidates or approved products; or

● merge  or  otherwise  enter  into  a  business  combination  with  another  company,  which  may  result  in  our
stockholders receiving cash and/or securities of the other company on terms that certain of our stockholders
may not deem desirable.

Our  insurance  policies  are  expensive  and  only  protect  us  from  some  business  risks,  which  leave  us  exposed  to
significant uninsured liabilities.

We do not carry insurance for all categories of risk that our business may encounter. Some of the policies we currently
maintain  include  general  liability,  employment  practices  liability,  property,  auto,  workers’  compensation,  cyber  liability,
products liability and directors’ and officers’ insurance. We do not know, however, if our current levels of coverage are
adequate or if we will be able to obtain insurance with adequate levels of coverage in the future, if at all. Any significant
uninsured  liability,  including  significant  uninsured  liabilities  resulting  from  COVID-19  or  related  government-imposed
shelter-in-place  mandates,  restrictions  on  travel  and  in-person  interactions,  business  closures  and  disruptions,  and  other
public health safety measures, may require us to pay substantial amounts, which could materially and adversely affect our

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financial  position  and  results  of  operations.  Furthermore,  any  increase  in  the  volatility  of  our  stock  price,  among  other
factors, may result in us being required to pay substantially higher premiums for our directors’ and officers’ insurance, and
may make it difficult for us to obtain adequate coverage on reasonable terms, if at all.

We must comply with environmental, health and safety laws and regulations.

Our activities involve the controlled storage, use and disposal of hazardous materials. We are subject to federal, state,
city and local laws and regulations, in and outside the United States, governing the use, manufacture, storage, handling and
disposal of these hazardous materials. Although we believe that the safety procedures we use for handling and disposing of
these materials comply with the standards prescribed by applicable laws and regulations, we cannot eliminate the risk of
accidental contamination or injury from these materials. In the event of an accident, regulatory authorities may curtail the
use of these materials and interrupt our business operations. We do not currently maintain hazardous materials insurance
coverage.

Failure to establish and maintain adequate financial infrastructure and accounting systems and controls could impair
our ability to comply with the financial reporting and internal controls requirements for publicly traded companies.

As  a  public  company,  we  operate  in  a  demanding  regulatory  environment,  which  requires  us  to  comply  with  the
Sarbanes-Oxley  Act  of  2002  and  related  rules  and  regulations,  expanded  disclosure  requirements,  accelerated  reporting
requirements and complex accounting rules. Responsibilities imposed by the Sarbanes-Oxley Act include establishing and
maintaining  corporate  oversight  and  adequate  internal  control  over  financial  reporting  and  disclosure  controls  and
procedures. Effective internal controls are necessary for us to produce reliable financial reports and are important to help
prevent financial fraud.

In particular, our compliance with Section 404 of the Sarbanes-Oxley Act has required and will continue to require that
we incur substantial accounting-related expenses and expend significant management efforts. Our testing, or the testing by
our  independent  registered  public  accounting  firm,  may  reveal  deficiencies  in  our  internal  controls  that  we  would  be
required to remediate in a timely manner. If we are not able to comply with the requirements of the Sarbanes-Oxley Act,
we  could  be  subject  to  sanctions  or  investigations  by  the  SEC,  the  Nasdaq  Global  Select  Market  or  other  regulatory
authorities,  which  would  require  additional  financial  and  management  resources  and  could  adversely  affect  the  market
price of our securities. Furthermore, if we cannot provide reliable financial reports or prevent fraud, including as a result of
remote  working  by  our  employees  in  connection  with  COVID-19  and  related  government-imposed  shelter-in-place
mandates and other public health safety measures, our business and results of operations would likely be materially and
adversely affected.

Our disclosure controls and procedures may not prevent or detect all errors or acts of fraud.

We are subject to the periodic reporting requirements of the Exchange Act. Our disclosure controls and procedures are
designed  to  reasonably  assure  that  information  required  to  be  disclosed  by  us  in  reports  we  file  or  submit  under  the
Exchange Act is accumulated and communicated to management, recorded, processed, summarized and reported within the
time periods specified in the rules and forms of the SEC. We believe that any disclosure controls and procedures or internal
controls and procedures, no matter how well conceived and operated, can provide only reasonable, not absolute, assurance
that the objectives of the control system are met.

These inherent limitations include the realities that judgments in decision-making can be faulty and that breakdowns
can occur because of simple error or mistake. Additionally, controls can be circumvented by the individual acts of some
persons, by collusion of two or more people or by an unauthorized override of the controls. Accordingly, because of the
inherent limitations in our control system, misstatements or insufficient disclosure due to error or fraud may occur and not
be detected.

Changes in our effective income tax rate could adversely affect our results of operations.

We  are  subject  to  income  taxes  in  the  United  States  and  various  foreign  jurisdictions.  Various  factors  may  have

favorable or unfavorable effects on our effective income tax rate. These factors include, but are not limited to,

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interpretations of existing tax laws, changes in tax laws and rates, such as the TCJA, the accounting for stock options and
other  stock-based  compensation,  changes  in  accounting  standards,  future  levels  of  research  and  development  spending,
changes in the mix and level of pre-tax earnings in different jurisdictions, the outcome of audits or other examinations by
the U.S. Internal Revenue Service and tax regulators in other jurisdictions, the accuracy of our estimates for unrecognized
tax benefits, the realization of deferred tax assets and changes to our ownership or capital structure.

The impact on our effective income tax rate resulting from these factors may be significant and could adversely affect

our results of operations.

If securities or industry analysts cease publishing research or reports about us, our business or our market, or if they
publish inaccurate or unfavorable reports about us or our securities, the price of our securities and trading volume in
our securities could decline.

The market for our common stock and the Convertible Notes depends in part on the research and reports that securities
or  industry  analysts  publish  about  our  company.  We  do  not  have  any  control  over  these  analysts,  and  there  can  be  no
assurance that analysts will continue to cover us or provide favorable coverage. If one or more of the analysts who cover us
downgrade  our  common  stock  or  publish  inaccurate  or  unfavorable  research  about  our  business,  our  stock  price  and  the
price of the Convertible Notes may decline. If one or more of the analysts covering us fail to regularly publish reports on
us, demand for our common stock and the Convertible Notes may decline, which could cause our stock price and the price
of the Convertible Notes and trading volume to decline.

Item 1B.  Unresolved Staff Comments

None.

Item 2.   Properties

Our corporate headquarters are located at 10 Hudson Yards in New York, New York, where we lease and occupy an
aggregate of approximately 45,600 square feet of office space. The lease covering this property is currently scheduled to
expire in March 2022.

Our research and development operations are based in San Diego, California, where we lease and occupy an aggregate
of approximately 34,000 square feet of space. The lease covering this property is currently scheduled to expire in October
2025.

We also lease and occupy approximately 8,600 square feet of office space in London, United Kingdom, which serves
as  the  headquarters  for  our  international  operations.  The  lease  covering  this  property  is  currently  scheduled  to  expire  in
May 2024.

We believe that our existing facilities are adequate for our immediate needs and that, should it be needed, additional

space can be leased to accommodate any future growth.

Item 3.   Legal Proceedings

For  a  description  of  our  significant  legal  proceedings,  see  Note  19  to  our  audited  consolidated  financial  statements

included elsewhere in this Annual Report on Form 10-K and incorporated by reference herein.

Item 4.   Mine Safety Disclosures

Not applicable.

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PART II

Item 5.   Market for Registrant’s Common Equity, Related Stockholder Matters and Issuer Purchases of Equity
Securities

Market Information and Stockholders

Our common stock trades on the Nasdaq Global Select Market under the symbol “ICPT”. As of December 31, 2020,
there were 33,015,614 shares of our common stock issued and outstanding and approximately 199 stockholders of record.
A  significantly  larger  number  of  stockholders  may  hold  their  shares  in  “street  name”  through  banks,  brokers  and  other
nominees. The number of stockholders of record does not include stockholders who hold their shares in “street name.”

Stock Price Performance Graph

The following graph compares the cumulative total stockholder return for our common stock to the cumulative total
stockholder return for the Nasdaq Composite Index and the Nasdaq Biotechnology Index, in each case, for the period from
December 31, 2015 through December 31, 2020. The graph assumes an initial investment of $100 in our common stock at
the closing price of $149.35 on December 31, 2015 and in the Nasdaq Composite Index and the Nasdaq Biotechnology
Index on December 31, 2015 and the reinvestment of dividends. The stock performance shown below is not intended to
forecast  or  be  indicative  of  the  possible  future  performance  of  our  common  stock,  and  we  do  not  make  or  endorse  any
predications  as  to  future  stockholder  returns.  The  following  stock  performance  information  shall  not  be  deemed  to  be
“soliciting material,” “filed” with the U.S. Securities and Exchange Commission (the “SEC”), incorporated by reference
into any filing under the Securities Act of 1933, as amended (the “Securities Act”), or the Securities Exchange Act of 1934,
as amended (the “Exchange Act”), or subject to the liabilities of Section 18 of the Exchange Act, except to the extent that
we specifically incorporate it by reference into a document filed under the Securities Act or the Exchange Act.

Among Intercept Pharmaceuticals, Inc., the Nasdaq Composite Index and

Comparison of Cumulative Total Return

the Nasdaq Biotechnology Index

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$100 investment in stock or index
Intercept Pharmaceuticals, Inc.
Nasdaq Composite Index
Nasdaq Biotechnology Index

Dividend Policy

2015

2016

2017

2018

2019

2020

December 31,

$ 100.00
$ 100.00
$ 100.00

$  72.75
$ 108.87
$  78.65

$  39.12
$ 141.13
$  95.67

$  67.49
$ 137.12
$  87.19

$  82.97
$  187.44
$  109.08

$  16.54
$  271.64
$  137.90

We have never declared or paid any cash dividends on our common stock, and we do not anticipate paying any cash

dividends in the foreseeable future.

Recent Sales of Unregistered Securities

Not applicable.

Issuer Purchases of Equity Securities

The  following  table  provides  certain  information  with  respect  to  purchases  of  our  common  stock  during  the  three

months ended December 31, 2020.

Period

October 1, 2020 through October 31, 2020
November 1, 2020 through November 30, 2020
December 1, 2020 through December 31, 2020

Total

Total Number
of Shares
Purchased (1)

 1,467
 1,297

$  42.08  
$  36.16  
 —  
$  39.30  

 — $

 2,764

Total Number of
Shares Purchased as
Part of Publicly

Average
Price Paid Announced Plans or
per Share

Programs

     Maximum Number (or

Approximate Dollar
Value) of Shares that
May Yet Be Purchased
Under the Plans or
Programs

 —  
 —  
 —  
 —  

 —
 —
 —
 —

(1) Represents shares of common stock withheld to satisfy taxes associated with the vesting of restricted stock awards.

Item 6.   Selected Financial Data

The selected consolidated financial data set forth below should be read together with “Management’s Discussion and
Analysis  of  Financial  Condition  and  Results  of  Operations”  and  our  audited  consolidated  financial  statements  and
accompanying notes included elsewhere in this Annual Report on Form 10-K. The selected consolidated financial data in
this  section  are  not  intended  to  replace  our  audited  consolidated  financial  statements  and  accompanying  notes.  Our
historical results are not necessarily indicative of our future results.

The selected consolidated statements of operations data for the years ended December 31, 2020, 2019 and 2018 and
the  selected  consolidated  balance  sheet  data  as  of  December  31,  2020  and  2019  have  been  derived  from  our  audited
consolidated financial statements and accompanying notes included elsewhere in this Annual Report on Form 10-K. The
selected consolidated statements of operations data for the years ended December 31, 2017 and 2016 and the selected

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consolidated balance sheet data as of December 31, 2018, 2017 and 2016 have been derived from our audited consolidated
financial statements and accompanying notes that are not included in this Annual Report on Form 10-K.

Consolidated Statement of Operations Data:
Revenue:

Product revenue, net
Licensing revenue
Total revenues
Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Restructuring

Total operating expenses
Operating loss

Total other income (expense), net
Net loss
Net loss per common and potential common share,
basic and diluted
Weighted average common and potential common
shares outstanding, basic and diluted

2020

Years Ended December 31, 
2017
2018
2019
(in thousands, except per share data)

2016

$  312,690
 —
 312,690

$  249,570
 2,432
 252,002

$  177,782
 2,022
 179,804

$  129,175
 1,781
 130,956

$

 18,169
 6,782
 24,951

 5,322
 332,493
 191,485
 14,630
 543,930
   (231,240)
 (43,640)

 2,519
 —
 255,474
 273,596
 207,301
 153,893
 —
 —
 465,294
 427,489
   (285,490)
   (402,538)
 (10,292)
 (23,752)
$ (274,880) $ (344,681) $ (309,242) $ (360,367) $  (412,830)

 1,371
 273,698
 191,499
 —
 466,568
   (335,612)
 (24,755)

 4,212
 317,418
 242,799
 —
 564,429
   (312,427)
 (32,254)

$

 (8.34) $

 (10.89) $

 (10.86) $

 (14.38) $

 (16.74)

 32,970

 31,654

 28,464

 25,054

 24,663

2020

2019

December 31, 
2018
(in thousands)

2017

2016

Consolidated Balance Sheet Data:
Cash, cash equivalents, restricted cash and
investment debt securities
Total assets
Accounts payable, accrued expenses and
other liabilities
Long-term debt (1)
Accumulated deficit
Total stockholders’ (deficit) equity

$

 477,170
 580,489

$

 657,347
 754,886

$

 436,160
 509,167

$

 414,917
 484,347

$

 689,385
 739,253

 171,039
 560,582
   (2,398,346)
 (166,853)

 153,968
 532,078
   (2,123,466)
 51,556

 105,109
 371,250
   (1,778,785)
 19,130

 94,777
 355,677
   (1,469,543)
 16,386

 65,551
 341,356
   (1,108,460)
 314,932

(1) Reflects  $690.0  million  aggregate  principal  amount  of  Convertible  Notes,  less  unamortized  debt  discounts  and
unamortized debt issuance costs as of December 31, 2020 and 2019 and $460.0 million aggregate principal amount of
2023  Convertible  Notes,  less  unamortized  debt  discounts  and  unamortized  debt  issuance  costs  as  of  December  31,
2018, 2017 and 2016. See Note 9 to our audited consolidated financial statements included elsewhere in this Annual
Report on Form 10-K for further information regarding the Convertible Notes.

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Item 7.   Management’s Discussion and Analysis of Financial Condition and Results of Operations

You should read the following discussion and analysis together with our audited consolidated financial statements and
accompanying  notes  included  elsewhere  in  this  Annual  Report  on  Form  10-K.  This  discussion  and  analysis  contains
forward-looking  statements,  which  involve  risks  and  uncertainties.  As  a  result  of  many  factors,  such  as  those  described
under “Cautionary Note Regarding Forward-Looking Statements,” “Risk Factors” and elsewhere in this Annual Report
on Form 10-K, our actual results may differ materially from those anticipated in these forward-looking statements.

Overview

We are a biopharmaceutical company focused on the development and commercialization of novel therapeutics to treat
progressive non-viral liver diseases with high unmet medical need utilizing our proprietary bile acid chemistry. Our first
marketed  product,  Ocaliva®  (obeticholic  acid  or  “OCA”),  is  a  farnesoid  X  receptor  (“FXR”)  agonist  approved  in  the
United States, the European Union and several other jurisdictions for the treatment of primary biliary cholangitis (“PBC”)
in combination with ursodeoxycholic acid (“UDCA”) in adults with an inadequate response to UDCA or as monotherapy
in adults unable to tolerate UDCA. In addition to commercializing OCA for PBC under the Ocaliva brand name, we are
currently  developing  OCA  for  additional  indications,  including  nonalcoholic  steatohepatitis  (“NASH”).  We  are  also
developing several product candidates in various stages of clinical and preclinical development. We believe that OCA and
our other product candidates have the potential to treat orphan and other more prevalent liver diseases such as NASH for
which there are currently limited therapeutic options.

Ocaliva  was  approved  for  PBC  by  the  U.S.  Food  and  Drug  Administration  (“FDA”)  in  May  2016  under  the
accelerated approval pathway. We commenced sales and marketing of Ocaliva in the United States shortly after receiving
approval,  and  Ocaliva  is  now  available  to  U.S.  patients  primarily  through  a  network  of  specialty  pharmacy  distributors.
Ocaliva received conditional approval for PBC from the European Commission in December 2016 and we commenced our
European  commercial  launch  in  January  2017.  We  have  submitted  dossiers  and  obtained,  or  are  otherwise  pursuing,
reimbursement from a number of national authorities in Europe. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia, and
we are pursuing marketing approval of Ocaliva for PBC in our other international target markets. Ocaliva received orphan
drug designation in both the United States and the European Union for the treatment of PBC. In addition, we continue to
work to execute on our post-marketing regulatory commitments with respect to Ocaliva in the U.S. and Europe.

Our  lead  product  candidate  is  OCA  for  the  potential  treatment  of  NASH.  In  February  2019,  we  announced  topline
results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in  patients  with  liver
fibrosis due to NASH, known as the REGENERATE trial. In the primary efficacy analysis, once-daily OCA 25 mg met the
primary endpoint agreed with the FDA of fibrosis improvement by at least one stage with no worsening of NASH at the
planned  18-month  interim  analysis.  Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most  common
were consistent with the known profile of OCA. Interim analysis results at 18 months were based on surrogate endpoints
and  the  impact  on  clinical  outcomes  has  not  been  confirmed.  The  REGENERATE  trial  is  ongoing  and  is  expected  to
continue through clinical outcomes for verification and description of the clinical benefit of OCA. OCA also achieved the
primary  endpoint  in  a  Phase  2b  clinical  trial  for  the  treatment  of  NASH  that  completed  in  late  July  2014,  known  as  the
FLINT trial, which was sponsored by the U.S. National Institute of Diabetes and Digestive and Kidney Diseases, a part of
the National Institutes of Health. OCA has received breakthrough therapy designation from the FDA for the treatment of
NASH  patients  with  liver  fibrosis.  In  September  2019,  we  submitted  a  New  Drug  Application  (“NDA”)  to  the  FDA
seeking accelerated approval of OCA for liver fibrosis due to NASH. In November 2019, the FDA accepted our NDA for
filing and granted a priority review designation of OCA for liver fibrosis due to NASH. In December 2019, we submitted a
Marketing  Authorization  Application  (“MAA”)  to  the  European  Medicines  Agency  (the  “EMA”)  seeking  conditional
approval of OCA for liver fibrosis due to NASH. In January 2020, the EMA validated our MAA and thereby confirmed
that  our  MAA  was  sufficiently  complete  to  begin  the  formal  review  process.  In  June  2020,  we  received  a  complete
response letter (“CRL”) from the FDA stating that our NDA for OCA for the treatment of liver fibrosis due to NASH could
not  be  approved  in  its  present  form.  The  CRL  indicated  that,  based  on  the  data  the  FDA  had  reviewed,  the  FDA  has
determined that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not
sufficiently outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due
to  NASH.  At  that  time,  the  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data
from the

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ongoing  REGENERATE  trial  in  support  of  potential  accelerated  approval  and  that  the  long-term  outcomes  phase  of  the
trial should continue. We are in discussions with the FDA with respect to the potential resubmission of our NDA seeking
accelerated approval of OCA for the treatment of liver fibrosis due to NASH. We had our end of review meeting with the
FDA in October 2020 to discuss the FDA’s risk-benefit assessment in the CRL based on its review of the available data, as
well  as  our  proposed  resubmission  of  our  NDA  for  the  treatment  of  liver  fibrosis  due  to  NASH.  The  meeting  was
constructive  and  the  FDA  has  provided  us  with  helpful  guidance  regarding  supplemental  data  we  can  provide  to  further
characterize OCA’s efficacy and safety profile that could support resubmission based on our Phase 3 REGENERATE 18-
month biopsy data, together with a safety update from our ongoing studies. We are advancing accordingly and plan to hold
additional meetings with the FDA with the goal of achieving sufficient alignment to proceed on this basis and potentially
resubmit our NDA for the treatment of liver fibrosis due to NASH by the end of 2021. In addition, we continue to work
collaboratively with the EMA on its review of our MAA.

As part of our product development activities, we expect to continue to invest in evaluating the potential of OCA in
progressive  non-viral  liver  diseases.  We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with
compensated cirrhosis, known as the REVERSE trial. In January 2020, we announced that we completed enrollment of the
REVERSE  trial  with  over  900  patients  randomized.  We  are  also  studying  OCA  in  combination  with  bezafibrate,  a  pan-
peroxisome  proliferator-activated  receptor  agonist,  in  patients  with  PBC  and  potentially  may  study  such  combination  in
other liver diseases. In addition, we have other compounds in early stages of research and development in our pipeline.

Capital Markets Activities During the Periods Under Review

In  May  2019,  we  issued  and  sold  (i)  2,760,000  shares  of  common  stock  in  a  registered  public  offering
(including  360,000  shares  issued  and  sold  upon  the  exercise  in  full  of  the  underwriters’  option  to  purchase  additional
shares), at a price to the public of $83.50 per share (the “2019 Public Offering”) and (ii) 119,760 shares of common stock
(the “2019 Private Placement Shares”) in a concurrent private placement of common stock (the “2019 Concurrent Private
Placement”) exempt from the registration requirements of the Securities Act of 1933, as amended (the “Securities Act”), at
a purchase price per share equivalent to the price to the public set in the 2019 Public Offering and pursuant to a securities
purchase agreement (the “2019 Securities Purchase Agreement”) that the Company entered into with Samsara BioCapital,
L.P.  (“Samsara”),  one  of  our  existing  stockholders.  Pursuant  to  the  2019  Securities  Purchase  Agreement,  we  granted  to
Samsara  certain  registration  rights  requiring  us,  upon  request  of  Samsara  on  or  after  July  9,  2019  and  subject  to  certain
terms and conditions, to register the resale by Samsara of its 2019 Private Placement Shares. Such registration rights expire
upon the earlier of (i) May 8, 2020 and (ii) the date that all of the 2019 Private Placement Shares have been sold or can be
sold publicly under Rule 144 of the Securities Act on a single day. We received net proceeds from the 2019 Public Offering
and  the  2019  Concurrent  Private  Placement  of  approximately  $227.3  million,  after  deducting  underwriting  discounts,
commissions and estimated offering expenses of approximately $13.9 million.

In May 2019, we also issued and sold $230.0 million aggregate principal amount of 2.00% Convertible Senior Notes
due 2026 (the “2026 Convertible Notes”). We received net proceeds from the sale of the 2026 Convertible Notes of $223.4
million,  after  deducting  underwriting  discounts,  commissions  and  estimated  offering  expenses  of  approximately  $6.6
million.

Financial Overview

Revenue

We  commenced  our  commercial  launch  of  Ocaliva  for  the  treatment  of  PBC  in  the  United  States  in  June  2016.  In
December  2016,  the  European  Commission  granted  conditional  approval  for  Ocaliva  for  the  treatment  of  PBC  and  we
commenced our European commercial launch in January 2017. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia. We
sell  Ocaliva  to  a  limited  number  of  specialty  pharmacies  which  dispense  the  product  directly  to  patients.  The  specialty
pharmacies are referred to as our customers.

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Product Revenue, Net

We recognize revenue upon shipment of Ocaliva to our customers. We provide the right of return to our customers for

unopened product for a limited time before and after its expiration date.

Under Accounting Standards Codification (“ASC”) Topic 606, Revenue from Contracts with Customers (“ASC 606”),
we have written contracts with each of our customers that have a single performance obligation — to deliver products upon
receipt of a customer order — and these obligations are satisfied when delivery occurs and the customer receives Ocaliva.
We  evaluate  the  creditworthiness  of  each  of  our  customers  to  determine  whether  collection  is  reasonably  assured.  We
estimate variable revenue by calculating gross product revenues based on the wholesale acquisition cost that we charge our
customers  for  Ocaliva,  and  then  estimating  our  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and
discounts  related  to  Medicare,  Medicaid  and  other  government  programs,  (ii)  estimated  costs  of  incentives  offered  to
certain indirect customers including patients and (iii) trade allowances, such as invoice discounts for prompt payment and
customer fees.

We recognized net sales of Ocaliva of $312.7 million, $249.6 and $177.8 million for the years ended December 31,

2020, 2019 and 2018, respectively.

We have received paragraph IV certification notice letters from several generic drug manufacturers indicating that each
such  company  has  submitted  to  the  FDA  an  Abbreviated  New  Drug  Application  (“ANDA”)  seeking  approval  to
manufacture and sell a generic version of our 5 mg and 10 mg dosage strengths of Ocaliva® (obeticholic acid) for PBC
prior  to  the  expiration  of  certain  patents  protecting  Ocaliva.  We  have  initiated  patent  infringement  suits  against  each  of
these  generic  drug  manufacturers  in  the  United  States  District  Court  for  the  District  of  Delaware.  While  we  intend  to
vigorously defend and enforce our intellectual property rights protecting Ocaliva, we can offer no assurance as to when the
lawsuits  will  be  decided,  whether  the  lawsuits  will  be  successful,  or  that  a  generic  equivalent  of  Ocaliva  will  not  be
approved  and  enter  the  market  before  the  expiration  of  such  patents.  See  Note  19  to  our  audited  consolidated  financial
statements included elsewhere in this Annual Report on Form 10-K for more information.

Licensing Revenue

In  March  2011,  we  entered  into  an  exclusive  license  agreement  (the  “Sumitomo  Agreement”)  with  Sumitomo
Dainippon Pharma Co., Ltd. (“Sumitomo Dainippon”), pursuant to which we granted to Sumitomo Dainippon an exclusive
license to research, develop and commercialize OCA for the treatment of PBC and NASH in Japan and China (excluding
Taiwan)  and  an  option  to  research,  develop  and  commercialize  OCA  in  certain  countries  outside  of  such  territories  (the
“Country Option”). We received an upfront payment from Sumitomo Dainippon of $15.0 million under the terms of the
Sumitomo Agreement. In October 2019, we and Sumitomo Dainippon mutually agreed to terminate with immediate effect
the Sumitomo Agreement. In connection with the termination of the Sumitomo Agreement, Sumitomo Dainippon agreed to
return  to  us  the  rights  to  develop  and  commercialize  OCA  in  China  and  we  agreed  to  forego  any  further  milestone  or
royalty payments relating to the development and commercialization of OCA in China. No payment was due from us to
Sumitomo Dainippon as a result of the termination of the Sumitomo Agreement.

We recognized licensing revenue of $0, $2.4 million and $2.0 million for the years ended December 31, 2020, 2019

and 2018, respectively.

Selling, General and Administrative Expenses

We have incurred and expect to continue to incur significant selling, general and administrative expenses as a result of,
among other initiatives, the launch and commercialization of Ocaliva for PBC in the United States, Europe and our other
target markets. In addition, we have incurred significant selling, general and administrative expenses and may in the future
incur similar expenses in connection with the preparation for the potential commercialization of OCA for liver fibrosis due
to NASH, if approved, and our other future approved products, if any, and any build-out of our general and administrative
infrastructure in the United States and abroad.

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Research and Development Expenses

Since  our  inception,  we  have  focused  significant  resources  on  our  research  and  development  activities,  including
conducting preclinical studies and clinical trials, pursuing regulatory approvals and engaging in other product development
activities. We recognize research and development expenses as they are incurred.

We have incurred and expect to continue to incur significant research and development expenses as a result of, among
other  initiatives,  our  clinical  development  programs  for  OCA  for  PBC  and  NASH,  our  other  earlier  stage  research
programs and our regulatory approval efforts.

Results of Operations

Comparison of the Years Ended December 31, 2020 and 2019

The following table summarizes our results of operations for the years ended December 31, 2020 and 2019:

Years Ended December 31, 

2020

2019

(in thousands)

Revenue:

Product revenue, net
Licensing revenue
Total revenue

Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Restructuring

Total operating expenses

Other income (expense):

Interest expense
Other income, net

Total other (expense), net

Net loss

Revenues

$  312,690

 —  

$  249,570
 2,432
 252,002

 312,690

 5,322
 332,493
 191,485
 14,630
 543,930

 4,212
 317,418
 242,799
 —
 564,429

 (48,054)
 4,414
 (43,640)

 (41,144)
 8,890
 (32,254)
$ (274,880) $ (344,681)

Product  revenue,  net  was  $312.7  million  and  $249.6  million  for  the  years  ended  December  31,  2020  and  2019,
respectively. For the years ended December 31, 2020 and 2019, product revenue, net was comprised of U.S. Ocaliva net
sales of $234.0 million and $187.5 million, respectively, and ex-U.S. Ocaliva net sales of $78.7 million and $62.1 million,
respectively. We commenced our commercial launch of Ocaliva for the treatment of PBC in the United States and certain
European countries in June 2016 and January 2017, respectively. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia. For
the years ended December 31, 2020 and 2019, licensing revenue was $0 and $2.4 million, respectively. In the case of the
year  ended  December  31,  2019,  revenues  were  related  to  the  amortization  of  upfront  payments  under  the  Sumitomo
Agreement.

Cost of sales

Cost of sales was $5.3 million and $4.2 million for the years ended December 31, 2020 and 2019, respectively. Our
cost of sales for the years ended December 31, 2020 and 2019 consisted primarily of packaging, labeling, materials and
related expenses.

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Selling, general and administrative expenses

Selling, general and administrative expenses were $332.5 million and $317.4 million for the years ended December
31,  2020  and  2019,  respectively.  The  $15.1  million  net  increase  between  periods  was  primarily  driven  by  increases  in
expenses during the first half of 2020 relating to our launch preparation activities associated with the potential approval and
commercialization of OCA for liver fibrosis due to NASH.

Research and development expenses

Research and development expenses were $191.5 million and $242.8 million for the years ended December 31, 2020
and 2019, respectively. The $51.3 million net decrease between periods was primarily driven by UK R&D tax credits of
$22.0  million  recognized  as  a  reduction  of  research  and  development  expenses  and  lower  NASH  development  costs,
including the conclusion of enrollment activities for the REGENERATE and REVERSE studies.

Restructuring expenses

Restructuring expenses were $14.6 million and $0 for the years ended December 31, 2020 and 2019, respectively. The
increase  between  periods  was  primarily  driven  by  severance  costs  and  other  related  termination  benefits  incurred  in
conjunction with the 2020 Workforce Plan.

Interest expense

Interest expense was $48.1 million and $41.1 million for the years ended December 31, 2020 and 2019, respectively.
For  the  years  ended  December  31,  2020  and  2019,  interest  expense  related  to  the  $230.0  million  aggregate  principal
amount of 2.00% Convertible Senior Notes due 2026 (the “2026 Convertible Notes”) that we issued in May 2019 and the
$460.0  million  aggregate  principal  amount  of  3.25%  Convertible  Senior  Notes  due  2023  (the  “2023  Convertible  Notes”
and together with the 2026 Convertible Notes, the “Convertible Notes”) that we issued in July 2016.

Other income, net

Other income, net was $4.4 million and $8.9 million for the years ended December 31, 2020 and 2019, respectively.

Such income is primarily attributable to interest income earned on cash, cash equivalents and investment debt securities.

Income taxes

For the years ended December 31, 2020 and 2019, no income tax expense or benefit was recognized. Our deferred tax
assets are comprised primarily of net operating loss carryforwards. We maintain a full valuation allowance on our deferred
tax assets since we have not yet achieved sustained profitable operations. As a result, we have not recorded any income tax
benefit since our inception.

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Comparison of the Years Ended December 31, 2019 and 2018

The following table summarizes our results of operations for the years ended December 31, 2019 and 2018:

Revenue:

Product revenue, net
Licensing revenue
Total revenue

Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Total operating expenses

Other income (expense):

Interest expense
Other income, net

Total other (expense), net

Net loss

Revenues

Years Ended December 31, 

2019

2018

(in thousands)

  $  249,570   $  177,782
 2,022
 179,804

 2,432  
 252,002  

 4,212
 317,418  
 242,799  
 564,429  

 2,519
 255,474
 207,301
 465,294

 (41,144) 
 8,890  
 (32,254) 
$  (344,681)

 (30,523)
 6,771
 (23,752)
$  (309,242)

Product  revenue,  net  was  $249.6  million  and  $177.8  million  for  the  years  ended  December  31,  2019  and  2018,
respectively. For the years ended December 31, 2019 and 2018, product revenue, net was comprised of U.S. Ocaliva net
sales of $187.5 million and $140.8 million, respectively, and ex-U.S. Ocaliva net sales of $62.1 million and $37.0 million,
respectively. We commenced our commercial launch of Ocaliva for the treatment of PBC in the United States and certain
European countries in June 2016 and January 2017, respectively. Since January 2017, Ocaliva has also received regulatory
approval in several of our target markets outside the United States and Europe, including Canada, Israel and Australia. For
the years ended December 31, 2019 and 2018, licensing revenue was $2.4 million and $2.0 million, respectively, in each
case, related to the amortization of upfront payments under the Sumitomo Agreement.

Cost of sales

Cost of sales was $4.2 million and $2.5 million for the years ended December 31, 2019 and 2018, respectively. Our
cost of sales for the years ended December 31, 2019 and 2018 consisted primarily of packaging, labeling, materials and
related expenses.

Selling, general and administrative expenses

Selling, general and administrative expenses were $317.4 million and $255.5 million for the years ended December
31,  2019  and  2018,  respectively.  The  $61.9  million  net  increase  between  periods  was  primarily  driven  by  increases  in
expenses relating to our launch preparation activities associated with the potential approval and commercialization of OCA
for liver fibrosis due to NASH.

Research and development expenses

Research and development expenses were $242.8 million and $207.3 million for the years ended December 31, 2019
and 2018, respectively. The $35.5 million net increase between periods was primarily driven by increases in OCA for liver
fibrosis  due  to  NASH  development  program  expenses  and  costs  associated  with  the  preparation  of  the  NASH  NDA
submission.

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Interest expense

Interest expense was $41.1 million and $30.5 million for the years ended December 31, 2019 and 2018, respectively.
For the year ended December 31, 2019, interest expense related to the 2026 Convertible Notes that we issued in May 2019
and the $460.0 million aggregate principal amount of 3.25% Convertible Senior Notes due 2023 (the “2023 Convertible
Notes” and together with the 2026 Convertible Notes, the “Convertible Notes”) that we issued in July 2016. For the year
ended December 31, 2018, interest expense related only to the 2023 Convertible Notes.

Other income, net

Other income, net was $8.9 million and $6.8 million for the years ended December 31, 2019 and 2018, respectively.

Such income is primarily attributable to interest income earned on cash, cash equivalents and investment debt securities.

Income Taxes

For the years ended December 31, 2019 and 2018, no income tax expense or benefit was recognized. Our deferred tax
assets are comprised primarily of net operating loss carryforwards. We maintain a full valuation allowance on our deferred
tax assets since we have not yet achieved sustained profitable operations. As a result, we have not recorded any income tax
benefit since our inception.

Liquidity and Capital Resources

Cash Flows

The following table sets forth the significant sources and uses of cash for the periods indicated:

Net cash (used in) provided by:

Operating activities
Investing activities
Financing activities
Effect of exchange rate changes
Net (decrease) increase in cash, cash equivalents and restricted cash

2020

Years Ended December 31, 
2019
(in thousands)

2018

$ (170,026) $ (236,613) $  (240,714)
 (48,070)
   (188,988)
 162,817
 263,545
 457,519
 (693)
 (1,526)
 (1,224)
 (386)
$  (26,765)
 (9,126) $  31,532

$

Operating Activities. Net cash used in operating activities of $170.0 million during the year ended December 31, 2020
was primarily a result of our $274.9 million net loss, partially offset by $60.8 million in stock-based compensation, $16.6
million for accretion of the discount on the 2023 Convertible Notes, $9.4 million for accretion of the discount on the 2026
Convertible  Notes,  $6.1  million  for  non-cash  operating  lease  costs,  $3.1  million  of  depreciation  and  a  net  increase  in
operating assets and liabilities of $2.0 million. Cash flows for the year ended December 31, 2020 include cash receipts of
$20.7 million reflecting payments from the HMRC for the U.K. R&D tax credit claims.

Net cash used in operating activities of $236.6 million during the year ended December 31, 2019 was primarily a result
of our $344.7 million net loss and a gain on lease termination of $2.0 million, partially offset by $56.0 million in stock-
based compensation, a net increase in operating assets and liabilities of $19.3 million, $15.3 million for accretion of the
discount  on  the  2023  Convertible  Notes,  $5.9  million  for  accretion  of  the  discount  on  the  2026  Convertible  Notes,  $5.4
million for non-cash operating lease costs, $3.7 million of depreciation and $2.7 million for loss on the disposal of fixed
assets.

Net cash used in operating activities of $240.7 million during the year ended December 31, 2018 was primarily a result
of our $309.2 million net loss and a net decrease in operating assets and liabilities of $2.8 million, partially offset by $49.9
million in stock-based compensation, $14.0 million for accretion of the discount on the 2023 Convertible Notes, and $4.6
million of depreciation.

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Investing Activities. For the year ended December 31, 2020, net cash provided by investing activities primarily reflects
the sales and maturities of investment debt securities of $497.4 million, partially offset by the purchases of investment debt
securities of $330.7 million.

For  the  year  ended  December  31,  2019,  net  cash  used  in  investing  activities  primarily  reflects  the  purchases  of

investment debt securities of $603.0 million, partially offset by the sales of investment debt securities of $415.2 million.

For  the  year  ended  December  31,  2018,  net  cash  used  in  investing  activities  primarily  reflects  the  purchase  of

investment debt securities of $436.1 million, partially offset by the sale of investment debt securities of $388.2 million.

Financing Activities. Net cash used in financing activities in the year ended December 31, 2020 consisted primarily of
$2.0  million  from  payments  of  employee  withholding  taxes  related  to  stock-based  awards  offset  by  $1.3  million  of  net
proceeds from the exercise of options to purchase common stock.

Net  cash  provided  by  financing  activities  in  the  year  ended  December  31,  2019  consisted  primarily  of  net  proceeds
received from the 2019 Public Offering and 2019 Concurrent Private Placement in May 2019 of $227.3 million and net
proceeds from the issuance of the 2026 Convertible Notes of $223.4 million.

Net cash provided by financing activities in the year ended December 31, 2018 consisted primarily of net proceeds of
approximately  $261.4  million  from  the  2018  Public  Offering  and  2018  Concurrent  Private  Placement  in  April  2018  and
$2.2  million  from  the  exercise  of  options  to  purchase  common  stock  net  of  payments  of  employee  withholding  taxes
related to stock-based awards.

2019 Public Offerings and 2019 Concurrent Private Placement

In May 2019, we issued and sold an aggregate of 2,879,760 shares of common stock in the 2019 Public Offering and
2019  Concurrent  Private  Placement.  We  received  net  proceeds  from  the  2019  Public  Offering  and  the  2019  Concurrent
Private  Placement  of  approximately  $227.3  million,  after  deducting  underwriting  discounts,  commissions  and  estimated
offering expenses of approximately $13.9 million.

2026 Convertible Notes

In May 2019, we issued and sold $230.0 million aggregate principal amount of 2.00% Convertible Senior Notes due
2026  (the  “2026  Convertible  Notes”).  We  received  net  proceeds  from  the  sale  of  the  2026  Convertible  Notes  of  $223.4
million,  after  deducting  underwriter  discounts,  commissions,  and  estimated  offering  expenses  of  approximately  $6.6
million.

The 2026 Convertible Notes were issued pursuant to a Second Supplemental Indenture, dated as of May 14, 2019 (the
“Second Supplemental Indenture”), which supplements the Indenture (the “Base Indenture”), as supplemented by a First
Supplemental  Indenture  (the  “First  Supplemental  Indenture”  and  collectively  with  the  Base  Indenture  and  the  Second
Supplemental  Indenture,  the  “Indenture”),  each  dated  as  of  July  6,  2016,  by  and  between  us  and  U.S.  Bank  National
Association, as trustee. The 2026 Convertible Notes are senior unsecured obligations of ours, bear interest at a fixed rate
of 2.00% per annum (payable semi-annually on May 15 and November 15 of each year, beginning on November 15, 2019)
and  will  mature  on  May  15,  2026,  unless  earlier  repurchased,  redeemed  or  converted.  The  2026  Convertible  Notes  are
convertible  at  the  option  of  holders,  under  certain  circumstances  and  during  certain  periods,  into  cash,  shares  of  our
common stock or a combination of cash and shares of our common stock, at our election. The initial conversion rate of the
2026  Convertible  Notes  is  9.2123  shares  of  our  common  stock  per  $1,000  principal  amount  of  2026  Convertible  Notes,
which is equivalent to an initial conversion price of approximately $108.55 per share of our common stock. The conversion
rate  is  subject  to  adjustment  in  some  events  but  will  not  be  adjusted  for  any  accrued  and  unpaid  interest.  In  addition,
following certain corporate events that occur prior to the maturity date, we will increase the conversion rate for a holder
who elects to convert its 2026 Convertible Notes in connection with such a corporate event in certain circumstances. If we
undergo  a  fundamental  change  (as  defined  in  the  Indenture),  holders  may  require  us  to  repurchase  for  cash  all  or  any
portion of their 2026 Convertible Notes at a fundamental change repurchase price equal to 100% of the principal amount

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of  the  2026  Convertible  Notes  to  be  repurchased,  plus  accrued  and  unpaid  interest  to,  but  excluding,  the  fundamental
change repurchase date. In addition, if certain make-whole fundamental changes occur, we will, in certain circumstances,
increase the conversion rate for any 2026 Convertible Notes converted in connection with such make-whole fundamental
change. We may not redeem the 2026 Convertible Notes prior to May 20, 2023. We may redeem for cash all or any portion
of the 2026 Convertible Notes, at our option, on or after May 20, 2023, under certain circumstances at a redemption price
equal to 100% or the principal amount of the 2026 Convertible Notes to be redeemed, plus accrued and unpaid interest to,
but excluding, the redemption date. The Indenture provides for customary events of default.

2018 Public Offering and 2018 Concurrent Private Placement

In April 2018, we issued and sold an aggregate of 4,257,813 shares of common stock in the 2018 Public Offering and
2018  Concurrent  Private  Placement.  We  received  net  proceeds  from  the  2018  Public  Offering  and  the  2018  Concurrent
Private  Placement  of  approximately  $261.4  million,  after  deducting  underwriting  discounts,  commissions  and  estimated
offering expenses of approximately $11.1 million.

Future Funding Requirements

As  of  December  31,  2020,  we  had  $477.2  million  in  cash,  cash  equivalents,  restricted  cash  and  investment  debt
securities. We currently expect to continue to incur significant operating expenses in the fiscal year ending December 31,
2021. These expenses are planned to support, among other initiatives, the continued commercialization of Ocaliva for PBC
in the United States and our other markets, our continued clinical development of OCA for PBC and NASH and our other
earlier stage research and development programs. Although we believe that our existing capital resources, together with our
net sales of Ocaliva for PBC, will be sufficient to fund our anticipated operating requirements for the next twelve months
following the filing of this report, we may need to raise additional capital to fund our operating requirements beyond that
period. Furthermore, in light of our receipt of the CRL from the FDA in June 2020 with respect to our NDA for OCA for
liver fibrosis due to NASH and the numerous risks and uncertainties associated with pharmaceutical product development
and  commercialization,  any  delays  in,  or  unanticipated  costs  associated  with,  our  development,  regulatory  or
commercialization  efforts  could  significantly  increase  the  amount  of  capital  required  by  us  to  fund  our  operating
requirements. Accordingly, we may seek to access the public or private capital markets whenever conditions are favorable,
even if we do not have an immediate need for additional capital at that time.

Our forecasts regarding the period of time that our existing capital resources will be sufficient to meet our operating
requirements  and  the  timing  of  our  future  funding  requirements,  both  near  and  long-term,  will  depend  on  a  variety  of
factors, many of which are outside of our control. Such factors include, but are not limited to:

● our ability to successfully commercialize Ocaliva for PBC;

● our ability to maintain our regulatory approval of Ocaliva for PBC in the United States, Europe, Canada, Israel,

Australia and other jurisdictions in which we have or may receive marketing authorization;

● our ability to timely and cost-effectively file for and obtain regulatory approval of our product candidates on an
accelerated basis or at all, including OCA for liver fibrosis due to NASH following the issuance of the CRL by
the  FDA;  any  advisory  committee  recommendation  or  dispute  resolution  determination  that  our  product
candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  should  not  be  approved  or  approved  only  under
certain  conditions;  or  any  future  determination  that  the  regulatory  applications  and  subsequent  information  we
submit  for  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  do  not  contain  adequate
clinical or other data or meet applicable regulatory requirements for approval;

● conditions  that  may  be  imposed  by  regulatory  authorities  on  our  marketing  approvals  for  our  products  and
product candidates, including OCA for liver fibrosis due to NASH, such as the need for clinical outcomes data
(and  not  just  results  based  on  achievement  of  a  surrogate  endpoint),  any  risk  mitigation  programs  such  as  a
REMS, and any related restrictions, limitations and/or warnings contained in the label of any of our products or
product candidates;

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● any  potential  side  effects  associated  with  Ocaliva  for  PBC,  OCA  for  liver  fibrosis  due  to  NASH  or  our  other
product candidates that could delay or prevent approval, require that an approved product be taken off the market,
require  the  inclusion  of  safety  warnings  or  precautions  or  otherwise  limit  the  sale  of  such  product  or  product
candidate, including in connection with the NISS relating to Ocaliva identified by the FDA in May 2020;

● the initiation, timing, cost, conduct, progress and results of our research and development activities, preclinical
studies  and  clinical  trials,  including  any  issues,  delays  or  failures  in  identifying  patients,  enrolling  patients,
treating  patients,  retaining  patients,  meeting  specific  endpoints  in  the  jurisdictions  in  which  we  intend  to  seek
approval or completing and timely reporting the results of our NASH or PBC clinical trials;

● the outcomes of ongoing discussions with the FDA and the EMA regarding the feasibility of the COBALT and

401 trials;

● our  ability  to  establish  and  maintain  relationships  with,  and  the  performance  of,  third-party  manufacturers,
contract research organizations and other vendors upon whom we are substantially dependent for, among other
things, the manufacture and supply of our products, including Ocaliva for PBC and, if approved, OCA for liver
fibrosis due to NASH, and our clinical trial activities;

● our  ability  to  identify,  develop  and  successfully  commercialize  our  products  and  product  candidates,  including

our ability to successfully launch OCA for liver fibrosis due to NASH, if approved;

● our  ability  to  obtain  and  maintain  intellectual  property  protection  for  our  products  and  product  candidates,
including our ability to cost-effectively file, prosecute, defend and enforce any patent claims or other intellectual
property rights;

● the size and growth of the markets for our products and product candidates and our ability to serve those markets;

● the degree of market acceptance of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH or our

other product candidates among physicians, patients and healthcare payors;

● the availability of adequate coverage and reimbursement from governmental and private healthcare payors for our
products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH, and our ability to
obtain adequate pricing for such products;

● our  ability  to  establish  and  maintain  effective  sales,  marketing  and  distribution  capabilities,  either  directly  or

through collaborations with third parties;

● competition from existing drugs or new drugs that become available;

● our ability to prevent system failures, data breaches or violations of data protection laws;

● costs  and  outcomes  relating  to  any  disputes,  governmental  inquiries  or  investigations,  regulatory  proceedings,
legal  proceedings  or  litigation,  including  any  securities,  intellectual  property,  employment,  product  liability  or
other litigation;

● our collaborators’ election to pursue research, development and commercialization activities;

● our  ability  to  establish  and  maintain  relationships  with  collaborators  with  development,  regulatory  and

commercialization expertise;

● our need for and ability to generate or obtain additional financing;

● our estimates regarding future expenses, revenues and capital requirements and the accuracy thereof;

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● our use of cash and short-term investments;

● our ability to acquire, license and invest in businesses, technologies, product candidates and products;

● our ability to attract and retain key personnel to manage our business effectively;

● our ability to manage the growth of our operations, infrastructure, personnel, systems and controls;

● our ability to obtain and maintain adequate insurance coverage;

● the  impact  of  COVID-19,  including  any  impact  on  our  results  of  operations  or  financial  position,  related
quarantines  and  government  actions,  delays  relating  to  our  regulatory  applications,  disruptions  relating  to  our
ongoing  clinical  trials  or  involving  our  contract  research  organizations,  study  sites  or  other  clinical  partners,
disruptions  relating  to  our  supply  chain  or  involving  our  third-party  manufacturers,  distributors  or  other
distribution partners, facility closures or other restrictions, and the extent and duration thereof;

● the impact of general U.S. and foreign economic, industry, market, regulatory or political conditions, including

the potential impact of Brexit; and

● the other risks and uncertainties identified under the captions “Risk Factors” and “Management’s Discussion and
Analysis of Financial Condition and Results of Operations” and elsewhere in this Annual Report on Form 10-K
and in our other periodic filings filed with the SEC.

We have no committed external sources of funding and additional funds may not be available when we need them on
terms that are acceptable to us, or at all. In addition, in recent months global markets have experienced significant volatility
in connection with concerns over the impact of COVID-19, and such concerns may in the future materially and adversely
affect  our  ability  to  raise  funds.  If  adequate  funds  are  not  available  to  us,  we  may  not  be  able  to  make  scheduled  debt
payments on a timely basis, or at all, and may be required to delay, limit, reduce or cease our operations.

Contractual Obligations

Our contractual obligations as of December 31, 2020 consisted primarily of obligations under the Convertible Notes,
and lease agreements. The following table summarizes our material contractual obligations as of December 31, 2020 and
the effect such obligations are expected to have on our liquidity and cash flows in future years:

Contractual Obligations:
Operating leases (1)
Convertible Notes (2)
Total

Payments Due By Period

Total

Less than 1 year 1 - 3 years 3 - 5 years

More than 5
years

(in thousands)

$  16,288 $
   752,100  
$ 768,388 $

 7,884 $

 5,759 $  2,645 $

 —
 19,550    491,625  
 9,200    231,725
 27,434 $ 497,384 $  11,845 $  231,725

(1) For a description of our material operating leases, see “Properties” above. The obligations represent payments for all
operating leases, including short-term operating leases exempt under ASC Topic 842, Leases (“ASC 842”) and leases
that  have  yet  to  commence.  Operating  expenses  associated  with  our  leased  office  buildings  are  not  included  in  the
table above.

(2) Represents 2023 Convertible Notes and 2026 Convertible Notes (including future interest payments at a fixed rate of

3.25% and 2.00% per year, respectively).

We  enter  into  contracts  in  the  normal  course  of  business  with  contract  research  organizations  for  our  clinical  trials,
contract  manufacturing  organizations  for  the  manufacture  and  supply  of  our  clinical  and  commercial  product  needs  and
other vendors for other research and development and commercial activities, as well as services and products for operating

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purposes. Our agreements generally provide for termination with notice. Such agreements are cancelable contracts and are
not included as purchase commitments.

Off-Balance Sheet Arrangements

As of December 31, 2020, we did not have any off-balance sheet arrangements.

Critical Accounting Policies and Estimates

Our management’s discussion and analysis of our financial condition and results of operations is based on our audited
consolidated financial statements, which we have prepared in accordance with accounting principles generally accepted in
the  United  States  of  America.  The  preparation  of  our  audited  consolidated  financial  statements  requires  us  to  make
estimates and judgments that affect the reported amounts of assets and liabilities, the disclosure of assets and liabilities at
the  date  of  the  financial  statements  and  the  reported  amounts  of  revenues  and  expenses  during  the  reporting  period.  We
evaluate these estimates and judgments on an ongoing basis. We base our estimates on historical experience and on various
other  factors  that  we  believe  are  reasonable  under  the  circumstances,  the  results  of  which  form  the  basis  for  making
judgments  about  the  carrying  value  of  assets  and  liabilities  that  are  not  readily  apparent  from  other  sources.  Our  actual
results could differ from these estimates.

While  our  significant  accounting  policies  are  more  fully  described  in  Note  2  to  our  audited  consolidated  financial
statements appearing elsewhere in this Annual Report on Form 10-K, we believe that the following accounting policies are
the most critical for fully understanding and evaluating our financial condition and results of operations.

Revenue Recognition

Effective January 1, 2018, we began recognizing revenue under ASC 606. The core principle of this revenue standard
is that a company should recognize revenue to depict the transfer of promised goods or services to customers in an amount
that reflects the consideration to which the company expects to be entitled in exchange for those goods or services. The
following five steps are applied to achieve that core principle: (i) identify the contract with the customer; (ii) identify the
performance  obligations  in  the  contract;  (iii)  determine  the  transaction  price;  (iv)  allocate  the  transaction  price  to  the
performance obligations in the contract and (v) recognize revenue when the company satisfies a performance obligation.

Product Revenue, Net

Under ASC 606, we have written contracts with each of our customers that have a single performance obligation — to
deliver  products  upon  receipt  of  a  customer  order  —  and  these  obligations  are  satisfied  when  delivery  occurs  and  the
customer receives Ocaliva. We evaluate the creditworthiness of each of our customers to determine whether collection is
reasonably assured. The wholesale acquisition cost that we charge our customers for Ocaliva is adjusted to arrive at our
estimated  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and  discounts,  (ii)  estimated  costs  of
incentives offered to certain indirect customers including patients, and (iii) trade allowances, such as invoice discounts for
prompt payment and customer fees.

Rebates and Discounts

We  contract  with  the  Centers  for  Medicare  &  Medicaid  Services  and  other  government  agencies  to  make  Ocaliva
available to eligible patients. As a result, we estimate any rebates and discounts and deduct these estimated amounts from
our gross product revenues at the time the revenues are recognized. Our estimates of rebates and discounts are based on the
government mandated discounts, which are statutorily-defined and applicable to these government funded programs, and
our historical experience with actual payments and redemptions. These estimates are recorded in accounts payable, accrued
expenses and other liabilities on our consolidated balance sheets.

We have been distributing and selling Ocaliva in Europe through our EU marketing authorization since 2017 and are
engaged in ongoing price discussions regarding the final price of Ocaliva within one of those jurisdictions. We recognize
net product revenues based on our estimate of consideration we expect to retain through final negotiations in that

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jurisdiction that will not be subject to a significant reversal. Our estimate is based on benchmarks of pricing approved in
other relevant European jurisdictions. We expect the difference between the amounts collected at the invoiced price and the
final price for OCA will be returned to the local government. If our estimates regarding the amounts to be refunded to the
government change, we will reflect the effect of the change in estimate in net product revenues in the period in which the
change in estimate occurs and will include any adjustments against all prior sales. These estimates are recorded in accounts
payable, accrued expenses and other liabilities on our consolidated balance sheets.

Other Incentives

Other incentives that we offer to indirect customers include co-pay assistance cards provided by us for PBC patients
who  reside  in  states  that  permit  co-pay  assistance  programs.  Our  co-pay  assistance  program  is  intended  to  reduce  each
participating patient’s portion of the financial responsibility for Ocaliva purchase price to a specified dollar amount. We
estimate the amount of co-pay assistance provided to eligible patients based on the terms of the program when product is
dispensed by the specialty pharmacies to the patients. These estimates are based on redemption information provided by
third-party claims processing organizations and are recorded in accounts payable, accrued expenses and other liabilities on
our consolidated balance sheets.

Trade Allowances

We  provide  invoice  discounts  on  Ocaliva  sales  to  certain  of  our  customers  for  prompt  payment  and  record  these
discounts as a reduction to gross product revenues. These discounts are based on contractual terms. Reserves for prompt
payment discounts are recorded in the same period the related revenue is recognized, resulting in a reduction of product
revenue and accounts receivable.

Valuation of Stock-Based Compensation

We account for stock-based compensation in accordance with ASC Topic 718, Compensation — Stock Compensation.
We estimate the fair value of stock option awards using the Black-Scholes option pricing model on the date of the grant.
The Black-Scholes option pricing model requires the use of assumptions, including with respect to stock price volatility,
assumed dividend yield, the expected term of options and the risk-free interest rate, as described below:

• The expected volatility is estimated based on actual historical volatility information of our own ordinary shares.

• The assumed dividend yield is based on our expectation of not paying dividends for the foreseeable future.

• The expected term of options granted represents the period of time the options are expected to be outstanding and is
based on the simplified method.

• The risk-free interest rate was based on the rate for U.S. Treasury securities at the date of grant with maturity dates
 approximately equal to the expected term of the award at the grant date.

Restricted stock unit awards and restricted stock awards without a market condition are valued based on the closing
price of our common stock on the date of the grant. The fair value of time-based equity awards is recognized and amortized
on a straight-line basis over the requisite service period of the award. The fair value of awards with market conditions is
estimated using the Monte Carlo simulation method and expense is recognized on a straight-line basis over the requisite
service  period  of  the  award.  The  Company  accounts  for  all  forfeitures  when  they  occur.  Ultimately,  the  actual  expense
recognized over the vesting period will be for only those shares that vest and are not forfeited.

We  expect  to  continue  to  grant  stock  options  and  other  stock-based  awards  and  the  impact  of  stock-based
compensation may fluctuate in future periods due to changes in the value of our common stock, changes to our headcount
and the number and value of awards granted.

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Convertible Senior Notes

The Convertible Notes are accounted for in accordance with ASC Subtopic 470-20, Debt with Conversion and Other
Options. ASC Subtopic 470-20 requires the issuer of convertible debt that may be settled in shares or cash upon conversion
at  the  issuer’s  option,  such  as  the  Convertible  Notes,  to  account  for  the  liability  (debt)  and  equity  (conversion  option)
components separately. The value assigned to the debt component is the estimated fair value, as of the issuance date, of a
similar debt instrument without the conversion option. The amount of the equity component (and resulting debt discount) is
calculated  by  deducting  the  fair  value  of  the  liability  component  from  the  principal  amount  of  the  convertible  debt
instrument. The resulting debt discount is amortized as additional non-cash interest expense over the expected life of the
notes utilizing the effective interest method. For additional information, see Note 9 to our audited consolidated financial
statements included elsewhere in this Annual Report on Form 10-K.

Income Taxes

We utilize the asset and liability method of accounting for income taxes. Under this method, deferred tax assets and
liabilities are determined based on the difference between the financial statement carrying amounts and tax bases of assets
and liabilities using enacted tax rates in effect for years in which the temporary differences are expected to reverse.

We determine the need for a valuation allowance by assessing the probability of realizing deferred tax assets, taking
into consideration all available positive and negative evidence, including historical operating results, expectations of future
taxable  income,  carryforward  periods  available,  various  income  tax  strategies  and  other  relevant  factors.  Significant
judgment is required in making this assessment and to the extent future expectations change, we would have to assess the
recoverability  of  our  deferred  assets  at  that  time.  At  December  31,  2020  and  2019,  we  maintained  a  full  valuation
allowance on our deferred tax assets.

Our tax returns are subject to examination by U.S. Federal, state, and foreign taxing jurisdictions. The impact of an
uncertain tax position taken or expected to be taken on an income tax return must be recognized in our financial statements
at the largest amount that is more likely than not to be sustained. An uncertain income tax position will not be recognized
in our financial statements unless it is more likely than not to be sustained. At December 31, 2020 and 2019, we had no
reserves for unrecognized tax benefits.

Recent Accounting Pronouncements

See Note 2 to our audited consolidated financial statements included elsewhere in this Annual Report on Form 10-K
for  a  full  description  of  recent  accounting  pronouncements  including  the  respective  expected  dates  of  adoption  and
expected effects, if any, on our results of operations and financial condition.

Item 7A.  Quantitative and Qualitative Disclosures about Market Risk

Our primary exposure to market risk is interest income sensitivity, which is affected by changes in the general level of
U.S.  interest  rates.  We  currently  do  not  hedge  interest  rate  exposure.  Because  of  the  short-term  maturities  of  our  cash
equivalents and investment debt securities, we do not believe that an increase in market rates would have any significant
impact on the realized value of our investment debt securities. If a hypothetical increase in interest rates of 100 basis points
were to have occurred on December 31, 2020, this change would not have had a material effect on the fair value of our
investment portfolio as of that date due to the conservative and short-term nature of these investments.

We  do  not  believe  that  our  cash,  cash  equivalents  and  investment  debt  securities  have  significant  risk  of  default  or
illiquidity. While we believe our cash, cash equivalents and investment debt securities do not contain excessive risk, we
cannot  provide  absolute  assurance  that,  in  the  future,  our  investments  will  not  be  subject  to  adverse  changes  in  market
value. In addition, we maintain significant amounts of cash and cash equivalents at one or more financial institutions that
are in excess of federally insured limits.

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We contract with CROs, investigational sites, suppliers, facilities, marketing firms and other vendors and suppliers in
Europe  and  internationally.  We  are  therefore  subject  to  fluctuations  in  foreign  currency  rates  in  connection  with  these
agreements. We do not hedge our foreign currency exchange rate risk.

Inflation generally affects us by increasing our cost of labor and clinical trial costs. We do not believe that inflation has

had a material effect on our results of operations during 2020, 2019 or 2018.

Item 8.   Financial Statements and Supplementary Data

The financial statements required to be filed pursuant to this Item 8 are appended to this Annual Report on Form 10-K
and  incorporated  by  reference  herein.  An  index  of  those  financial  statements  is  set  forth  under  Item  15.  “Exhibits  and
Financial Statement Schedules”.

Item 9.   Changes in and Disagreements With Accountants on Accounting and Financial Disclosure

None.

Item 9A.  Controls and Procedures

Evaluation of Disclosure Controls and Procedures

Our  Chief  Executive  Officer  and  Chief  Financial  Officer  evaluated  the  effectiveness  of  our  disclosure  controls  and
procedures  as  of  December  31,  2020.  The  term  “disclosure  controls  and  procedures,”  as  defined  in  Rules  13a-15(e)  and
15d-15(e)  under  the  Exchange  Act,  means  controls  and  other  procedures  of  a  company  that  are  designed  to  ensure  that
information  required  to  be  disclosed  by  a  company  in  the  reports  that  it  files  or  submits  under  the  Exchange  Act  is
recorded, processed, summarized and reported, within the time periods specified in the SEC’s rules and forms. Disclosure
controls and procedures include, without limitation, controls and procedures designed to ensure that information required
to  be  disclosed  by  a  company  in  the  reports  that  it  files  or  submits  under  the  Exchange  Act  is  accumulated  and
communicated  to  the  company’s  management,  including  its  principal  executive  and  principal  financial  officers,  as
appropriate  to  allow  timely  decisions  regarding  required  disclosure.  Management  recognizes  that  any  controls  and
procedures, no matter how well designed and operated, can provide only reasonable assurance of achieving their objectives
and  management  necessarily  applies  its  judgment  in  evaluating  the  cost-benefit  relationship  of  possible  controls  and
procedures.  Based  on  the  evaluation  of  our  disclosure  controls  and  procedures  as  of  December  31,  2020,  our  Chief
Executive Officer and Chief Financial Officer concluded that, as of such date, our disclosure controls and procedures were
effective at the reasonable assurance level.

Management’s Report on Internal Control Over Financial Reporting

Our  management  is  responsible  for  establishing  and  maintaining  adequate  internal  control  over  financial  reporting.
Internal control over financial reporting is defined in Rules 13a-15(f) and 15d-15(f) under the Exchange Act, as a process
designed by, or under the supervision of, the company’s principal executive and principal financial officers and effected by
the  company’s  board  of  directors,  management  and  other  personnel,  to  provide  reasonable  assurance  regarding  the
reliability  of  financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles and includes those policies and procedures that: (i) pertain to the maintenance of
records that in reasonable detail accurately and fairly reflect the transactions and dispositions of the assets of the company;
(ii) provide reasonable assurance that transactions are recorded as necessary to permit preparation of financial statements in
accordance  with  generally  accepted  accounting  principles,  and  that  receipts  and  expenditures  of  our  company  are  being
made  only  in  accordance  with  authorizations  of  management  and  directors  of  the  company;  and  (iii)  provide  reasonable
assurance regarding prevention or timely detection of unauthorized acquisition, use, or disposition of our company’s assets
that could have a material effect on the financial statements.

All  internal  controls,  no  matter  how  well  designed,  have  inherent  limitations.  Therefore,  even  those  systems
determined  to  be  effective  can  provide  only  reasonable  assurance  with  respect  to  consolidated  financial  statement
preparation and presentation. Because of its inherent limitations, internal control over financial reporting may not prevent

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or detect misstatements. Also, projections of any evaluation of effectiveness to future periods are subject to the risk that
controls may become inadequate because of changes in conditions, or that the degree of compliance with the policies or
procedures may deteriorate.

Our  management,  with  the  participation  of  our  Chief  Executive  Officer  and  Chief  Financial  Officer,  assessed  the
effectiveness of our internal control over financial reporting as of December 31, 2020, based on criteria established in the
Internal Control — Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of the Treadway
Commission (COSO). Based on that assessment, management concluded that our internal control over financial reporting
was effective as of December 31, 2020.

Attestation Report of Independent Registered Public Accounting Firm

The effectiveness of our internal control over financial reporting as of December 31, 2020 has been audited by KPMG
LLP, an independent registered public accounting firm, as stated in their report included elsewhere in this Annual Report
on Form 10-K.

Changes in Internal Control Over Financial Reporting

There  were  no  changes  in  our  internal  control  over  financial  reporting  that  occurred  during  the  quarter  ended
December  31,  2020  that  have  materially  affected,  or  are  reasonably  likely  to  materially  affect,  our  internal  control  over
financial reporting.

Item 9B.  Other Information

Not applicable.

Item 10.  Directors, Executive Officers and Corporate Governance

PART III

We have adopted a Global Code of Business Conduct as our “code of ethics,” as defined by regulations promulgated
under the Securities Act of 1933, as amended, and the Securities Exchange Act of 1934, as amended, which applies to our
directors, officers and employees, including our principal executive officer, principal financial officer, principal accounting
officer  or  controller,  or  persons  performing  similar  functions.  The  Global  Code  of  Business  Conduct  is  available  on  our
website  at  www.interceptpharma.com  in  the  Investors  &  Media  section  under  “Corporate  Governance.”  We  intend  to
satisfy  the  disclosure  requirement  under  Item  5.05  of  Form  8-K  regarding  any  future  amendment  to,  or  waiver  from,  a
provision of the Global Code of Business Conduct that applies to our principal executive officer, principal financial officer,
principal  accounting  officer  or  controller,  or  persons  performing  similar  functions  by  posting  such  information  on  our
website at www.interceptpharma.com in the Investors & Media section under “Corporate Governance.” The references to
www.interceptpharma.com herein are inactive textual references only, and the information found on our internet website is
not incorporated by reference into this Annual Report on Form 10-K or any other report we file with or furnish to the SEC.

The remainder of the information required by this item is incorporated by reference to our definitive proxy statement
related to our 2021 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after
the end of the fiscal year covered by this Annual Report on Form 10-K.

Item 11.  Executive Compensation

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2021 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

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Item 12.  Security Ownership of Certain Beneficial Owners and Management and Related Stockholder Matters

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2021 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

Item 13.  Certain Relationships and Related Transactions, and Director Independence

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2021 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

Item 14.  Principal Accounting Fees and Services

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2021 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

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PART IV

Item 15.  Exhibits and Financial Statement Schedules

(a) 1. Index to Consolidated Financial Statements

Reports of Independent Registered Public Accounting Firm
Consolidated Balance Sheets
Consolidated Statements of Operations
Consolidated Statements of Comprehensive Loss
Consolidated Statements of Changes in Stockholders’ Equity
Consolidated Statements of Cash Flows
Notes to Consolidated Financial Statements

2. Index to Consolidated Financial Statements

F-2
F-6
F-7
F-8
F-9
F-10
F-11

Financial  statement  schedules  have  been  omitted  from  this  Annual  Report  on  Form  10-K  because  they  are  not
applicable,  not  required  or  the  information  required  is  set  forth  in  the  audited  consolidated  financial  statements  or
accompanying notes.

3. Exhibits

The exhibits filed or furnished as part of this Annual Report on Form 10-K are set forth in the Exhibit Index below,

which is incorporated herein by reference.

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Exhibit
Number     

3.1

3.2

4.1

4.2

4.3

4.4

4.5

4.6

4.7

4.8

4.9

Exhibit Index

Exhibit Description

Restated Certificate of Incorporation, as
amended

Incorporated herein by reference

Form†
Form 10-Q

     Exhibit     
3.1

Filing Date
August 10, 2020

Restated Bylaws

Form 10-Q

Form of Common Stock Certificate

Form S-8(1)

3.2

4.3

August 10, 2020

November 7,
2012

Indenture, dated as of July 6, 2016, between the
Registrant and U.S. Bank National Association,
as trustee

First Supplemental Indenture (including the
Form of Note), dated as of July 6, 2016,
between the Registrant and U.S. Bank National
Association, as trustee

Form of Senior Indenture

Form of Subordinated Indenture

Form of Senior Note

Form of Subordinated Note

Securities Purchase Agreement, dated April 4,
2018, between the Registrant and the
purchasers named therein

Securities Purchase Agreement, dated May 8,
2019, between the Registrant and the
purchasers named therein

Form 8-K

4.1

July 6, 2016

Form 8-K

4.2

July 6, 2016

Form S-3(2)

Form S-3(2)

Form S-3(2)

Form S-3(2)

4.1

4.2

4.3

4.4

May 10, 2017

May 10, 2017

May 10, 2017

May 10, 2017

Form 8-K

10.1

April 10, 2018

Form 8-K

10.1

May 14, 2019

Form 8-K

4.2

May 14, 2019

4.10

Second Supplemental Indenture (including the
Form of Note), dated as of May 14, 2019,
between the Registrant and U.S. Bank National
Association, as trustee

4.11*

Description of Securities of the Registrant

10.1#

10.2#

10.3#

10.4#

Intercept Pharmaceuticals, Inc. 2012 Equity
Incentive Plan

Form S-1/A(3)

10.2.1

September 27,
2012

Form of Stock Option Grant Notice and
Agreement for Directors

Form 10-Q

10.1

August 10, 2020

Form of Stock Option Grant Notice and
Agreement for Employees and Consultants

Form 10-K

10.3

February 25,
2020

Form of Restricted Stock Unit Award Grant
Notice and Agreement for Directors

Form 10-Q

10.2

August 10, 2020

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10.5#

10.6#

10.7#

10.8#

10.9#

Form of Restricted Stock Unit Award Grant
Notice and Agreement for Employees and
Consultants

Form 10-K

10.5

February 25,
2020

Form of Restricted Stock Award Grant Notice
and Agreement for Directors

Form 10-Q

10.3 

May 9, 2014

Form of Restricted Stock Award Grant Notice
and Agreement for Employees and Consultants

Form 10-Q

10.4 

May 9, 2014

Form of Performance Stock Unit Grant Notice
and Agreement

Form 10-K

10.8 

February 25,
2020

Form of Performance Share Grant Notice and
Agreement

Form 10-Q

10.6 

May 10, 2018

10.10# Amended and Restated Employment

Form 10-Q

10.5 

May 14, 2013

Agreement, effective May 14, 2013, between
the Registrant and Mark Pruzanski

10.11#

Employment Agreement, effective May 3, 2016,
between the Registrant and Sandip S. Kapadia

Form 10-Q

10.1.1

August 9, 2016

10.12#

Employment Agreement, effective February 15,
2017, between the Registrant and Jerome B.
Durso

Form 10-Q

10.1 

May 10, 2017

10.13#

Employment Agreement, effective April 14,
2017, between the Registrant and David Ford

Form 10-Q

10.1 

August 3, 2017

10.14# Amended and Restated Employment

Form 8-K

10.2 

Agreement, effective as of November 27, 2017,
between the Registrant and David Shapiro

December 1,
2017

10.15#

Employment Agreement, effective January 22,
2018, between the Registrant and Ryan Sullivan

Form 10-Q

10.1 

August 8, 2019

10.16#

10.17#

Employment Agreement, effective February 6,
2018, between the Registrant and Gail
Cawkwell

Employment Agreement, effective November
19, 2019, between the Registrant and Jason
Campagna

Form 10-Q

10.2 

August 8, 2019

Form 10-K

10.17

February 25,
2020

10.18#

Employment Agreement, effective June 20,
2015, between the Registrant and Richard Kim

Form 10-Q

10.3

August 10, 2020

10.19#

Retirement and Consulting Agreement, dated as
of December 9, 2020, between the Registrant
and Mark Pruzanski, M.D.

Form 8-K

10.2

10.20# Amended and Restated Employment

Form 8-K

10.1

Agreement, dated as of December 9, 2020,
between the Registrant and Jerome Durso

December 10,
2020

December 10,
2020

10.21#* Employment Agreement, effective as of

December 18, 2020, between the Registrant and
Jared Freedberg

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10.22#

Form of Indemnification Agreement for
directors and executive officers of the
Registrant

Form S-1(3)

10.7 

September 4,
2012

10.23

10.24

10.25

10.26

10.27

10.28

10.29

10.30

10.31

10.32

10.33

10.34

10.35

10.36

Base Call Option Confirmation, dated June 30,
2016, between the Registrant and Royal Bank
of Canada

Base Call Option Confirmation, dated June 30,
2016, between the Registrant and UBS AG,
London Branch

Base Call Option Confirmation, dated June 30,
2016, between the Registrant and Credit Suisse
Capital LLC

Additional Call Option Confirmation, dated
July 1, 2016, between the Registrant and Royal
Bank of Canada

Additional Call Option Confirmation, dated
July 1, 2016, between the Registrant and UBS
AG, London Branch

Additional Call Option Confirmation, dated
July 1, 2016, between the Registrant and Credit
Suisse Capital LLC

Form 8-K

10.1 

July 6, 2016

Form 8-K

10.3 

July 6, 2016

Form 8-K

10.5 

July 6, 2016

Form 8-K

10.2 

July 6, 2016

Form 8-K

10.4 

July 6, 2016

Form 8-K

10.6 

July 6, 2016

Lease Agreement between The Irvine Company
LLC and the Registrant, dated May 1, 2014

Form 8-K

10.1 

May 7, 2014

Form 10-Q

10.7 

November 9,
2016

Form 10-Q

10.1 

August 7, 2018

Form 10-Q

10.1 

Form 10-K

10.12 

November 1,
2018

February 29,
2016

Form 10-K

10.17  March 1, 2017

Form 10-Q

10.1 

November 6,
2017

Form 10-Q

10.2 

August 7, 2018

Second Amendment to Lease, dated as of July
19, 2016, between the Registrant and Irvine
Eastgate Office II LLC

Third Amendment to Lease, dated as of June
21, 2018, between the Registrant and Irvine
Eastgate Office II LLC

Fourth Amendment to Lease, dated as of
October 30, 2018, between the Registrant and
Irvine Eastgate Office II LLC

Underlease between the Registrant, Intercept
Pharma Europe Ltd. and Performing Right
Society, Ltd., dated January 22, 2016

Lease Agreement, dated December 7, 2016,
between the Registrant and Legacy Yards
Tenant LP

First Amendment to Lease Agreement, dated
June 27, 2017, between the Registrant and
Legacy Yards Tenant LP

Second Amendment to Lease, dated June 22,
2018, between the Registrant and Legacy Yards
Tenant LP

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10.37

10.38

Third Amendment to Lease, dated November 1,
2019, between the Registrant and Legacy Yards
Tenant LP

Form 10-Q

10.1

Termination of Lease, dated December 31,
2017, between the Registrant and One Hudson
Yards Owner LLC

Form 10-K

10.21 

November 5,
2019

February 28,
2018

10.39*++ Commercial Manufacturing and Supply

Agreement, dated August 12, 2016, between
the Registrant and PharmaZell GMBH

10.40+

Amendment #1 to Manufacturing and Supply
Agreement, dated December 12, 2017, between
the Registrant and PharmaZell GMBH

Form 10-K

10.2.1

February 28,
2018

10.41*++ Sumitomo Agreement, dated March 29, 2011,

between the Registrant and Sumitomo
Dainippon Pharma Co., Ltd.

10.42

10.43

Amendment No. 1, dated June 8, 2011, to that
certain Sumitomo Agreement, dated March 29,
2011, between the Registrant and Sumitomo
Dainippon Pharma Co., Ltd.

Amendment No. 2, dated September 16, 2011,
to that certain Sumitomo Agreement, dated
March 29, 2011, between the Registrant and
Sumitomo Dainippon Pharma Co., Ltd.

10.44+

Amendment No. 3, dated February 13, 2018, to
that certain Sumitomo Agreement, dated March
29, 2011, between the Registrant and
Sumitomo Dainippon Pharma Co., Ltd.

Form 10-Q

10.1 

May 10, 2018

Form 10-Q

10.2 

May 10, 2018

Form 10-Q

10.3 

May 10, 2018

10.45

Letter Agreement, dated October 25, 2019,
between the Registrant and Sumitomo
Dainippon Pharma Co., Ltd.

Form 10-K

10.41

February 25,
2020

21.1*

Subsidiaries of the Registrant

23.1*

24.1*

31.1*

31.2*

Consent of Independent Registered Public
Accounting Firm

Power of Attorney (included in signature page
to this Annual Report on Form 10-K)

Certification of Principal Executive Officer
required by Rule 13a-14(a) or Rule 15d-14(a)

Certification of Principal Financial Officer
required by Rule 13a-14(a) or Rule 15d-14(a)

114

Table of Contents

32.1*
(4)

101*

Certifications required by Rule 13a-14(b) or
Rule 15d-14(b) and Section 1350 of Chapter 63
of Title 18 of the United States Code (18 U.S.C.
1350)

The following materials from the Registrant’s
Annual Report on Form 10-K for the year ended
December 31, 2020, formatted in Inline XBRL
(eXtensible Business Reporting Language): (i)
Consolidated Balance Sheets as of December
31, 2020 and 2019, (ii) Consolidated Statements
of Operations for the Years Ended December
31, 2020, 2019 and 2018, (iii) Consolidated
Statement of Comprehensive Loss for the Years
Ended December 31, 2020, 2019 and 2018, (iv)
Consolidated Statements of Changes in
Stockholders’ (Deficit) Equity for the Years
Ended December 31, 2020, 2019 and 2018, (v)
Consolidated Statements of Cash Flows for the
Years Ended December 31, 2020, 2019 and
2018 and (vi) Notes to Consolidated Financial
Statements

104*

Cover Page Interactive Data File (formatted as
Inline XBRL and contained in Exhibit 101)

*

Filed herewith.

+ Confidential treatment has been received with respect to certain portions of this exhibit. Omitted portions have been

filed separately with the Securities and Exchange Commission (“SEC”).

++ Portions of the exhibit have been omitted pursuant to Regulation S-K, Item 601(b)(10)(iv).

#

Indicates a management contract or compensatory plan or arrangement.

† Unless otherwise specified, the File No. is 001-35668.

(1) Registration Statement on Form S-8 filed by the Registrant, Registration No. 333-184810.

(2) Registration Statement on Form S-1 filed by the Registrant, Registration No. 333-217861.

(3) Registration Statement on Form S-1 filed by the Registrant, Registration No. 333-183706.

(4) This certification “accompanies” the Annual Report on Form 10-K to which it relates, is not deemed filed with the
SEC  and  is  not  to  be  incorporated  by  reference  into  any  filing  of  Registrant  under  the  Securities  Act  of  1933,  as
amended, or the Securities Exchange Act of 1934, as amended, (whether made before or after the date of the Annual
Report on Form 10-K), irrespective of any general incorporation language contained in such filing.

Item 16.  Form 10-K Summary

None.

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Pursuant to the requirements of Section 13 or 15(d) of the Securities Exchange Act of 1934, the registrant has duly

caused this report to be signed on its behalf by the undersigned, thereunto duly authorized.

SIGNATURES

Date: February 25, 2021

    By:/s/ Jerome Durso

INTERCEPT PHARMACEUTICALS, INC.

Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

Date: February 25, 2021

By:/s/ Sandip Kapadia
Sandip Kapadia
Chief Financial Officer and Treasurer
(Principal Financial Officer and Principal Accounting Officer)

POWER OF ATTORNEY

KNOW ALL PERSONS BY THESE PRESENTS, that each person whose signature appears below hereby constitutes
and  appoints  Jerome  Durso  and  Sandip  Kapadia,  and  each  of  them,  as  his  or  her  true  and  lawful  attorneys-in-fact  and
agents, with full power of substitution and resubstitution, for him or her, and in his or her name, place and stead, in any and
all capacities, to sign any and all amendments to this Annual Report on Form 10-K, and to file the same, with all exhibits
thereto,  and  all  other  documents  in  connection  therewith,  with  the  Securities  and  Exchange  Commission,  granting  unto
each said attorney-in-fact and agent full power and authority to do and perform each and every act and thing required or
necessary  to  be  done  in  and  about  the  premises,  as  fully  and  to  all  intents  and  purposes  as  the  undersigned  could  do  in
person,  and  hereby  ratifying  and  confirming  all  that  said  attorneys-in-fact  and  agents,  or  any  of  them  or  their  or  his
substitute or substitutes, may lawfully do or cause to be done by virtue hereof.

Pursuant  to  the  requirements  of  the  Securities  Exchange  Act  of  1934,  this  report  has  been  signed  below  by  the

following persons on behalf of the registrant and in the capacities indicated on February 25, 2021.

Signature

/s/ Jerome Durso
Jerome Durso

/s/ Sandip Kapadia
Sandip Kapadia

/s/ Paolo Fundarò
Paolo Fundarò

/s/ Srinivas Akkaraju, M.D., Ph.D.
Srinivas Akkaraju, M.D., Ph.D.

/s/ Luca Benatti, Ph.D.
Luca Benatti, Ph.D.

/s/ Daniel Bradbury
Daniel Bradbury

Title

President and Chief Executive Officer and Director
(Principal Executive Officer)

Chief Financial Officer and Treasurer
(Principal Financial Officer and Principal Accounting Officer)

Chairman of the Board of Directors

Director

Director

Director

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/s/ Keith Gottesdiener, M.D.
Keith Gottesdiener, M.D.

/s/ Nancy Miller-Rich
Nancy Miller-Rich

/s/ Mark Pruzanski, M.D.
Mark Pruzanski, M.D.

/s/ Gino Santini
Gino Santini

/s/ Glenn Sblendorio
Glenn Sblendorio

/s/ Daniel Welch
Daniel Welch

Director

Director

Director

Director

Director

Director

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INTERCEPT PHARMACEUTICALS, INC.

Index to Consolidated Financial Statements

Reports of Independent Registered Public Accounting Firm
Consolidated Financial Statements:
Consolidated Balance Sheets as of December 31, 2020 and 2019
Consolidated Statements of Operations for the Years Ended December 31, 2020, 2019 and 2018
Consolidated Statements of Comprehensive Loss for the Years Ended December 31, 2020, 2019 and 2018
Consolidated Statements of Changes in Stockholders’ (Deficit) Equity for the Years Ended December 31, 2020, 2019
and 2018

Consolidated Statements of Cash Flows for the Years Ended December 31, 2020, 2019 and 2018
Notes to Consolidated Financial Statements

F-2

F-6
F-7
F-8

F-9
F-
10
F-11

F-1

Table of Contents

REPORT OF INDEPENDENT REGISTERED PUBLIC ACCOUNTING FIRM

To the Stockholders and Board of Directors
Intercept Pharmaceuticals, Inc.:

Opinion on the Consolidated Financial Statements

We  have  audited  the  accompanying  consolidated  balance  sheets  of  Intercept  Pharmaceuticals,  Inc.  and  subsidiaries  (the
Company)  as  of  December  31,  2020  and  2019,  the  related  consolidated  statements  of  operations,  comprehensive  loss,
changes in stockholders’ (deficit) equity, and cash flows for each of the years in the three-year period ended December 31,
2020, and the related notes (collectively, the consolidated financial statements). In our opinion, the consolidated financial
statements present fairly, in all material respects, the financial position of the Company as of December 31, 2020 and 2019,
and the results of its operations and its cash flows for each of the years in the three-year period ended December 31, 2020,
in conformity with U.S. generally accepted accounting principles.

We  also  have  audited,  in  accordance  with  the  standards  of  the  Public  Company  Accounting  Oversight  Board  (United
States)  (PCAOB),  the  Company’s  internal  control  over  financial  reporting  as  of  December  31,  2020,  based  on  criteria
established in Internal Control – Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of
the Treadway Commission, and our report dated February 25, 2021 expressed an unqualified opinion on the effectiveness
of the Company’s internal control over financial reporting.

Basis for Opinion

These  consolidated  financial  statements  are  the  responsibility  of  the  Company’s  management.  Our  responsibility  is  to
express  an  opinion  on  these  consolidated  financial  statements  based  on  our  audits.  We  are  a  public  accounting  firm
registered with the PCAOB and are required to be independent with respect to the Company in accordance with the U.S.
federal  securities  laws  and  the  applicable  rules  and  regulations  of  the  Securities  and  Exchange  Commission  and  the
PCAOB.

We  conducted  our  audits  in  accordance  with  the  standards  of  the  PCAOB.  Those  standards  require  that  we  plan  and
perform the audit to obtain reasonable assurance about whether the consolidated financial statements are free of material
misstatement,  whether  due  to  error  or  fraud.  Our  audits  included  performing  procedures  to  assess  the  risks  of  material
misstatement  of  the  consolidated  financial  statements,  whether  due  to  error  or  fraud,  and  performing  procedures  that
respond  to  those  risks.  Such  procedures  included  examining,  on  a  test  basis,  evidence  regarding  the  amounts  and
disclosures in the consolidated financial statements. Our audits also included evaluating the accounting principles used and
significant  estimates  made  by  management,  as  well  as  evaluating  the  overall  presentation  of  the  consolidated  financial
statements. We believe that our audits provide a reasonable basis for our opinion.

Critical Audit Matter

The critical audit matter communicated below is a matter arising from the current period audit of the consolidated financial
statements that was communicated or required to be communicated to the audit committee and that: (1) relates to accounts
or  disclosures  that  are  material  to  the  consolidated  financial  statements  and  (2)  involved  our  especially  challenging,
subjective, or complex judgment. The communication of a critical audit matter does not alter in any way our opinion on the
consolidated  financial  statements,  taken  as  a  whole,  and  we  are  not,  by  communicating  the  critical  audit  matter  below,
providing a separate opinion on the critical audit matter or on the accounts or disclosures to which it relates.

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Table of Contents

Assessing deductions from revenue related to certain rebates and discounts accruals

As discussed in Note 2 to the consolidated financial statements, the Company records net product revenue by deducting
rebates  and  discounts,  among  other  items.  The  rebates  and  discounts  are  related  to  arrangements  with  the  Centers  for
Medicare  &  Medicaid  Services  and  other  government  agencies,  and  are  estimated  and  accrued  with  a  corresponding
reduction  of  gross  product  revenues  when  revenue  is  recognized.  The  Company  had  $27.4  million  and  $9.5  million  in
rebates  and  discounts  accruals  as  of  December  31,  2020  for  a  European  jurisdiction  in  which  final  pricing  is  subject  to
ongoing negotiations with the government, and for all other jurisdictions, respectively, which were recorded in accounts
payable, accrued expenses and other liabilities on the consolidated balance sheet.

We identified the assessment of deductions from revenue related to certain rebates and discounts accruals as a critical audit
matter  because  evaluating  the  Company’s  assumptions  involved  especially  challenging  auditor  judgment,  including
specialized  knowledge  of  the  regulatory  environment  in  a  particular  European  jurisdiction.  Rebates  and  discounts  are
estimated  based  on  certain  assumptions  developed  using  benchmarks  of  pricing  approved  in  other  relevant  European
jurisdictions  in  the  case  of  the  European  jurisdiction  in  which  final  pricing  is  subject  to  ongoing  negotiations  with  the
government, and, for all other jurisdictions, historical experience with actual payments and redemptions.

The following are the primary procedures we performed to address this critical audit matter. We evaluated the design and
tested the operating effectiveness of certain internal controls over the Company’s rebates and discounts accruals process,
including controls related to the significant assumptions used in the Company’s estimation of certain rebates and discounts.
We evaluated the Company’s ability to estimate rebates and discounts by comparing the previously recorded accruals to the
actual amounts that were settled and ultimately paid by the Company. We assessed the Company’s current period estimates
by comparing the accrued amounts to historical payments and redemptions. We also performed sensitivity analyses based
on potential changes in certain assumptions and assessed the impact relative to the Company’s accruals as of December 31,
2020. In addition, we involved professionals with specialized skills and knowledge of the regulatory environment in the
European  jurisdiction  in  which  final  pricing  is  subject  to  ongoing  negotiations  with  the  government,  who  assisted  in
assessing the Company’s assumptions in estimating the rebates and discounts.

/s/ KPMG LLP

We have served as the Company’s auditor since 2008.

New York, New York
February 25, 2021

F-3

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REPORT OF INDEPENDENT REGISTERED PUBLIC ACCOUNTING FIRM

To the Stockholders and Board of Directors
Intercept Pharmaceuticals, Inc.:

Opinion on Internal Control Over Financial Reporting

We have audited Intercept Pharmaceuticals, Inc. and subsidiaries’ (the Company) internal control over financial reporting
as of December 31, 2020, based on criteria established in Internal Control – Integrated Framework (2013) issued by the
Committee  of  Sponsoring  Organizations  of  the  Treadway  Commission.  In  our  opinion,  the  Company  maintained,  in  all
material respects, effective internal control over financial reporting as of December 31, 2020, based on criteria established
in Internal Control – Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of the Treadway
Commission.

We  also  have  audited,  in  accordance  with  the  standards  of  the  Public  Company  Accounting  Oversight  Board  (United
States)  (PCAOB),  the  consolidated  balance  sheets  of  the  Company  as  of  December  31,  2020  and  2019,  the  related
consolidated  statements  of  operations,  comprehensive  loss,  changes  in  stockholders’  (deficit)  equity,  and  cash  flows  for
each of the years in the three-year period ended December 31, 2020, and the related notes (collectively, the consolidated
financial  statements),  and  our  report  dated  February  25,  2021  expressed  an  unqualified  opinion  on  those  consolidated
financial statements.

Basis for Opinion

The Company’s management is responsible for maintaining effective internal control over financial reporting and for its
assessment of the effectiveness of internal control over financial reporting, included in the accompanying Management’s
Report on Internal Control over Financial Reporting. Our responsibility is to express an opinion on the Company’s internal
control over financial reporting based on our audit. We are a public accounting firm registered with the PCAOB and are
required  to  be  independent  with  respect  to  the  Company  in  accordance  with  the  U.S.  federal  securities  laws  and  the
applicable rules and regulations of the Securities and Exchange Commission and the PCAOB.

We conducted our audit in accordance with the standards of the PCAOB. Those standards require that we plan and perform
the audit to obtain reasonable assurance about whether effective internal control over financial reporting was maintained in
all material respects. Our audit of internal control over financial reporting included obtaining an understanding of internal
control over financial reporting, assessing the risk that a material weakness exists, and testing and evaluating the design
and operating effectiveness of internal control based on the assessed risk. Our audit also included performing such other
procedures as we considered necessary in the circumstances. We believe that our audit provides a reasonable basis for our
opinion.

Definition and Limitations of Internal Control Over Financial Reporting

A company’s internal control over financial reporting is a process designed to provide reasonable assurance regarding the
reliability  of  financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles. A company’s internal control over financial reporting includes those policies and
procedures  that  (1)  pertain  to  the  maintenance  of  records  that,  in  reasonable  detail,  accurately  and  fairly  reflect  the
transactions and dispositions of the assets of the company; (2) provide reasonable assurance that transactions are recorded
as necessary to permit preparation of financial statements in accordance with generally accepted accounting principles, and
that receipts and expenditures of the company are being made only in accordance with authorizations of management and
directors of the company; and (3) provide reasonable assurance regarding prevention or timely detection of unauthorized
acquisition, use, or disposition of the company’s assets that could have a material effect on the financial statements.

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Because of its inherent limitations, internal control over financial reporting may not prevent or detect misstatements. Also,
projections of any evaluation of effectiveness to future periods are subject to the risk that controls may become inadequate
because of changes in conditions, or that the degree of compliance with the policies or procedures may deteriorate.

/s/ KPMG LLP

New York, New York
February 25, 2021

F-5

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

Consolidated Balance Sheets

Current assets:

Assets

Cash and cash equivalents
Restricted cash
Investment debt securities, available-for-sale
Accounts receivable, net of allowance for credit losses of $235 and $0,
respectively
Prepaid expenses and other current assets

Total current assets

Fixed assets, net
Inventory
Security deposits
Other assets

Total assets

Liabilities and Stockholders’ (Deficit) Equity

Current liabilities:

Accounts payable, accrued expenses and other liabilities
Short-term interest payable
Total current liabilities

Long-term liabilities:

Long-term debt
Long-term other liabilities

Total liabilities

Commitments and contingencies (Note 19)
Stockholders’ (deficit) equity:

Common stock par value $0.001 per share; 90,000,000 and 45,000,000 shares
authorized; 33,015,614 and 32,853,066 shares issued and outstanding as of
December 31, 2020 and 2019, respectively
Additional paid-in capital
Accumulated other comprehensive loss, net
Accumulated deficit

Total stockholders’ (deficit) equity
Total liabilities and stockholders’ (deficit) equity

December 31, 

2020

2019

(in thousands, except share and per share
data)

$

$

$

$

$

58,151
7,503
411,516

41,549
27,022
545,741
6,326
9,027
7,068
12,327
580,489

171,039
8,037
179,076

560,582
7,684
747,342

33
2,233,937
(2,477)
(2,398,346)
(166,853)
580,489

$

$

$

$

$

70,055
4,725
582,567

38,044
25,924
721,315
5,202
8,462
6,661
13,246
754,886

153,968
8,037
162,005

532,078
9,247
703,330

33
2,176,133
(1,144)
(2,123,466)
51,556
754,886

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Operations

Revenue:

Product revenue, net
Licensing revenue
Total revenue
Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Restructuring

Total operating expenses
Operating loss

Other income (expense):

Interest expense
Other income, net

Total other (expense), net

Net loss
Net loss per common and potential common share:

Basic and diluted

Weighted average common and potential common shares
outstanding:

Basic and diluted

2020

Years Ended December 31, 
2019
(in thousands, except per share data)

2018

$

312,690

$
—  

312,690

$

249,570
2,432
252,002

177,782
2,022
179,804

5,322
332,493
191,485
14,630
543,930
(231,240)

(48,054)
4,414
(43,640)
(274,880)

(8.34)

$

$

4,212
317,418
242,799
—
564,429
(312,427)

(41,144)
8,890
(32,254)
(344,681)

(10.89)

$

$

2,519
255,474
207,301
—
465,294
(285,490)

(30,523)
6,771
(23,752)
(309,242)

(10.86)

$

$

32,970

31,654

28,464

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Comprehensive Loss

Net loss
Other comprehensive (loss) income:
   Net changes related to available-for-sale investment debt securities:
     Unrealized (losses) gains on investment debt securities
     Reclassification adjustment for realized gains on investment debt securities 
included in other income, net
   Net unrealized (losses) gains on investment debt securities
     Foreign currency translation losses
   Other comprehensive (loss) income
Comprehensive loss

2020

Years Ended December 31, 
2019
(in thousands)
$ (274,880) $ (344,681) $ (309,242)

2018

(202)

1,509

88

$

(135)
(337) $
(996)
(1,333)

(8)
80
(1,553)
(1,473)
$ (276,213) $ (343,559) $ (310,715)

(8)
1,501
(379)
1,122

$

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Changes in Stockholders’ (Deficit) Equity

For the Years Ended December 31, 2020, 2019 and 2018
(in thousands)

Common Stock

Paid-in

Comprehensive

Accumulated

Stockholders’

Additional

Other

Total

Accumulated

Balance - December 31, 2017
Stock-based compensation
Issuance of common stock from public
and private placement offerings, net of
underwriting fees and issuance costs
Net proceeds from exercise of stock
options
Employee withholding taxes related to
stock-based awards
Other comprehensive loss
Net loss
Balance - December 31, 2018
Stock-based compensation
Recognition of debt discount on 2026
Convertible Notes
Issuance of common stock from public
and private placement offerings, net of
underwriting fees and issuance costs
Net proceeds from exercise of stock
options
Employee withholding taxes related to
stock-based awards
Other comprehensive income
Net loss
Balance - December 31, 2019
Stock-based compensation
Net proceeds from exercise of stock
options
Employee withholding taxes related to
stock-based awards
Other comprehensive loss
Net loss
Balance - December 31, 2020

Shares      Amount     
$
25,173

25

—   —  

Capital
$ 1,486,690
49,914

$

4,258

263

5

—

261,357

4,363

—

—
—   —  
—   —  

(2,180)
—
—  
$

$ 1,800,144
55,982

85,915

227,257

8,993

$

29,694
—

—

2,880

279

—
—
—
32,853

$

30
—

—

3

—

—
—
—
33

—   —  

Loss, Net

Deficit

(786) $ (1,469,543) $
—  

—  

     Equity (Deficit)
16,386
49,914

—

—

—
(1,473)

—

—

—
—  

—  

(309,242)

(2,259) $ (1,778,785) $

—

—

—

—

—

—

—

—

261,362

4,363

(2,180)
(1,473)
(309,242)
19,130
55,982

85,915

227,260

8,993

(2,158)
1,115
(344,681)
51,556
60,850

(2,158)
—
—
$ 2,176,133
60,850

—
1,115
—

—
—
(344,681)

$

(1,144) $ (2,123,466) $
—  

—  

176

—

(1,052)

—

—

(1,052)

—

(13)
—   —  
—   —  

(1,994)
—
—  
$

—
(1,333)

—
—  

—  

(274,880)

(2,477) $ (2,398,346) $

(1,994)
(1,333)
(274,880)
(166,853)

33,016

$

33

$ 2,233,937

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Cash Flows

Cash flows from operating activities:

Net loss
Adjustments to reconcile net loss to net cash used in operating activities:
Stock-based compensation
(Accretion) amortization of (discount) premium on investment debt securities
Amortization of deferred financing costs
Realized loss on investments
Depreciation
Non-cash operating lease cost
Gain on lease termination
Loss on the disposal of fixed assets
Accretion of debt discount
Provision for allowance of credit losses, net of write-offs
Changes in operating assets:

Accounts receivable
Prepaid expenses and other current assets
Inventory
Security deposits
Other assets

Changes in operating liabilities:

Accounts payable, accrued expenses and other current liabilities
Operating lease liabilities
Interest payable
Deferred revenue
Long-term other liabilities

Net cash (used in) operating activities

Cash flows from investing activities:

Purchases of investment debt securities
Sales and maturities of investment debt securities
Purchases of equipment, leasehold improvements, and furniture and fixtures
Net cash provided by (used in) investing activities

Cash flows from financing activities:

Proceeds from issuance of 2026 Convertible Notes, net of issuance costs
Proceeds from issuance of common stock, net of issuance costs
Proceeds from exercise of options, net
Payments of employee withholding taxes related to stock-based awards

Net cash (used in) provided by financing activities

Effect of exchange rate changes on cash, cash equivalents and restricted cash
Net (decrease) increase in cash, cash equivalents and restricted cash

Cash, cash equivalents and restricted cash at beginning of period
Cash, cash equivalents and restricted cash at end of period
Supplemental disclosure of non-cash transactions:

Right-of-use asset obtained in exchange for new operating lease obligations

Non-cash investing and financing activities
   Net increase in accrued fixed assets

Reconciliation of cash, cash equivalents and restricted cash included in the condensed
consolidated balance sheets:
Cash and cash equivalents
Restricted cash
Total cash, cash equivalents and restricted cash

2020

Years Ended December 31, 
2019
(in thousands)

2018

$

(274,880)

$

(344,681)

$ (309,242)

60,850
4,006
2,540
—
3,118
6,142
—
—  

25,964
235

(2,646)
(3,075)
(269)
(269)
1,385

13,863
(6,990)
—
—  
—
(170,026)

(330,713)
497,421
(3,891)
162,817

—
—
1,301
(1,994)
(693)
(1,224)
(9,126)
74,780
65,654

4,721

368

58,151
7,503
65,654

$

$

$

$

$

55,982
(302)
2,130
—
3,663
5,388
(1,995)
2,682
21,189
—

(12,350)
(5,353)
(1,354)
2,562
(24,665)

56,411
(6,767)
562
(2,432)
12,717
(236,613)

(603,014)
415,162
(1,136)
(188,988)

223,424
227,260
8,993
(2,158)
457,519
(386)
31,532
43,248
74,780

49,914
(33)
1,542
8
4,582
—
—
1,331
14,031
—

(9,193)
(3,682)
(3,628)
7,153
—

10,332
—
—
(2,022)
(1,807)
(240,714)

(436,071)
388,168
(167)
(48,070)

—
261,362
4,363
(2,180)
263,545
(1,526)
(26,765)
70,013
43,248

$

— $

— $

—

—

70,055
4,725
74,780

$

$

43,248
—
43,248

$

$

$

$

$

See accompanying notes to consolidated financial statements

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Table of Contents

1. Overview of Business

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Intercept  Pharmaceuticals,  Inc.  (the  “Company”)  is  a  biopharmaceutical  company  focused  on  the  development  and
commercialization of novel therapeutics to treat progressive non-viral liver diseases, including primary biliary cholangitis
(“PBC”)  and  nonalcoholic  steatohepatitis  (“NASH”).  The  Company  currently  has  one  marketed  product,  Ocaliva
(obeticholic acid or “OCA”). Founded in 2002 in New York, the Company has operations in the United States, Europe and
Canada.

2. Summary of Significant Accounting Policies

Basis of Presentation and Principles of Consolidation

The Company’s financial statements have been prepared in conformity with accounting principles generally accepted
in  the  United  States  of  America  (“U.S.  GAAP”).  The  consolidated  financial  statements  include  the  accounts  of  the
Company  and  its  wholly  owned  subsidiaries.  All  intercompany  balances  and  transactions  have  been  eliminated  in
consolidation. The Company has no unconsolidated subsidiaries or investments accounted for under the equity method.

Use of Estimates

The preparation of these financial statements in conformity with U.S. GAAP requires management to make estimates
and judgments that affect the reported amounts of assets and liabilities, the disclosure of assets and liabilities at the date of
the  consolidated  financial  statements  and  the  reported  amounts  of  revenues  and  expenses  during  the  reporting  period.
Actual results could differ from these estimates.

Foreign Currency

The Company’s functional and reporting currency is the U.S. dollar. Transactions in foreign currencies are recorded at
the exchange rate prevailing on the date of the transaction. The resulting monetary assets and liabilities are translated into
U.S.  dollars  at  exchange  rates  prevailing  on  the  subsequent  balance  sheet  date.  Revenue  and  expense  components  are
translated to U.S. dollars at weighted-average exchange rates in effect during the period. Foreign currency transaction gains
and  losses  resulting  from  remeasurement  are  recognized  in  Other  income,  net  within  the  consolidated  statements  of
operations.  Gains  and  losses  as  a  result  of  foreign  currency  translation  adjustments  are  recorded  as  a  component  of
Accumulated other comprehensive loss, net in the equity/(deficit) section of our consolidated balance sheets and as Foreign
currency translation gains (losses) within the accompanying consolidated statements of comprehensive loss.

Cash and Cash Equivalents

The Company considers all highly liquid securities with an original or remaining maturity of three months or less at

acquisition to be cash equivalents.

Restricted Cash

Restricted cash relates to short-term bank guarantees which provides financial assurance that the Company will fulfill
certain customer obligations entered into in the normal course of business. The cash is restricted as to withdrawal or use
while the related bank guarantee in favor of the customer is outstanding.

Credit Losses

The allowance for credit losses is based on the Company’s assessment of the collectibility of customer accounts. The

Company regularly reviews the allowance by considering factors such as historical experience, the aging of the accounts

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

receivable balances, credit conditions that may affect a customer’s ability to pay, current and forecast economic conditions
and other relevant factors.

The following table summarizes the allowance for credit losses activity on the Company’s trade receivables for the

year ended December 31, 2020 (in thousands):

Balance at December 31, 2019
   Provision for credit losses
   Write-offs
Balance at December 31, 2020

$

$

—
258
(23)
235

For available-for-sale investment debt securities in an unrealized loss position, the Company first assesses whether it
intends to sell the security or it is more likely than not that it will be required to sell the security before recovery of its
amortized  cost  basis.  If  either  of  the  criteria  regarding  intent  or  requirement  to  sell  is  met,  the  amortized  cost  basis  is
written down to fair value through income. For any investment debt securities that do not meet the criteria, the Company
evaluates  whether  the  decline  in  fair  value  has  resulted  from  credit  losses  or  other  factors.  Management  considers  the
extent in which the fair value of the security is less than amortized costs, any changes to the rating of the security by a
rating agency, changes in interest rates, and any other adverse factors related to the security. If the assessment indicates a
credit loss, the present value of cash flows expected to be collected are compared to the amortized cost basis of the security.
If the expected present value of cash flows is less than the amortized cost basis, a credit loss exists and an allowance for
credit losses is recorded, limited to the amount that the fair value is below the amortized cost basis. Any impairment not
recorded through an allowance is recognized in Other comprehensive (loss) income.

Changes in the allowance for credit losses are recorded as a provision for (or reversal of) credit loss expense. Losses
are charged against the allowance when management believes the uncollectibility of the security is confirmed or whether
either of the criteria regarding intent or requirement to sell is met.

The Company excludes accrued interest from both the fair value and amortized cost basis in the assessment of credit
losses  on  its  available-for-sale  investment  debt  securities  and  will  instead  elect  to  write-off  any  uncollectible  accrued
interest receivable balances in a timely manner, which is defined by the Company as when interest due becomes 90 days
delinquent.

Investment Debt Securities, Available-For-Sale

Investment debt securities are considered to be available-for-sale and are carried at fair market value. The estimated
fair  value  of  the  available-for-sale  investment  debt  securities  is  determined  based  on  quoted  market  prices  or  rates  for
similar instruments. Unrealized gains and losses, if any, are reported in accumulated other comprehensive income (loss).
The  cost  of  investment  debt  securities  is  adjusted  for  amortization  of  premiums  and  accretion  of  discounts  to  maturity.
Such amortization and accretion is included in Other income, net. Realized gains and losses are included in Other income,
net. Interest and dividends on available-for-sale securities are included in Other income, net.

Fair Value of Financial Instruments

The carrying amounts of certain financial instruments, including cash and cash equivalents, restricted cash, accounts
receivable, prepaid expenses and other current assets, accounts payable, accrued expenses and other liabilities approximate
fair value due to their short-term maturities.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Concentration of Credit Risk

Financial  instruments,  which  potentially  subject  the  Company  to  concentrations  of  credit  risk,  principally  consist  of

cash, cash equivalents, investment debt securities and accounts receivables from customers.

The  Company  currently  invests  its  excess  cash  primarily  in  money  market  funds,  and  high  quality,  marketable  debt
instruments  of  corporations,  financial  institutions  and  government  sponsored  enterprises.  The  Company  has  adopted  an
investment policy that includes guidelines relative to credit quality, diversification and maturities to preserve principal and
liquidity.

On a consolidated basis, for the year ended December 31, 2020, the Company’s three largest customers (as discussed
in  more  detail  below  under  “Revenue  Recognition”)  accounted  for  31%,  30%  and  14%,  of  the  Company’s  net  product
sales, respectively. On a consolidated basis, for the year ended December 31, 2019, the Company’s three largest customers
(as discussed in more detail below under “Revenue Recognition”) accounted for 32%, 31% and 15%, of the Company’s net
product sales, respectively. On a consolidated basis, for the year ended December 31, 2018, the Company’s three largest
customers  (as  discussed  in  more  detail  below  under  “Revenue  Recognition”)  accounted  for  38%,  28%  and  16%,  of  the
Company’s net product sales, respectively.

On  a  consolidated  basis,  the  Company’s  three  largest  customers  accounted  for  31%,  17%  and  10%  of  the
December  31,  2020  accounts  receivable  balance,  respectively.  On  a  consolidated  basis,  the  Company’s  three  largest
customers  accounted  for  27%,  28%  and  7%  of  the  December  31,  2019  accounts  receivable  balance,  respectively.  The
Company monitors its customers’ financial credit worthiness in order to assess and respond to any changes in their credit
profile.

Accounts Receivable

The Company extends credit to customers based on its evaluation of the customer’s financial condition. The Company
records receivables for all billings when amounts are due under standard terms. Accounts receivable are stated at amounts
due  net  of  applicable  prompt  pay  discounts  and  other  contractual  adjustments  as  well  as  an  allowance  for  doubtful
accounts. The Company will write off accounts receivable when the Company determines that they are uncollectible. The
Company  has  recorded  $41.5  million  and  $38.0  million  of  accounts  receivable  as  of  December  31,  2020  and  2019,
respectively, and has recorded an allowance for any credit losses of $0.2 million and $0 as of December 31, 2020 and 2019,
respectively.

Fixed Assets

Fixed assets are stated at cost, and depreciated over the estimated useful life of the assets. Depreciation is recorded
using  the  straight-line  method  over  the  estimated  useful  lives  of  the  respective  assets,  generally  three  to  seven  years.
Leasehold improvements are amortized over the shorter of the asset’s useful life or the life of the lease term. Expenditures
for maintenance and repairs are charged to expense as incurred. Upon sale or retirement of assets, the cost of the assets
disposed of and the related accumulated depreciation are removed from the balance sheets and any related gains or losses
are reflected in the consolidated statements of operations.

Impairment of Long-Lived Assets

Long-lived  assets  consist  of  fixed  assets  and  right-of-use  assets.  The  Company  evaluates  long-lived  assets  for
impairment  when  events  and  circumstances  indicate  that  the  carrying  amount  of  an  asset  or  group  of  assets  may  not  be
fully  recoverable.  If  indicators  of  impairment  exist,  the  Company  assesses  the  recoverability  of  the  affected  long-lived
assets by determining whether the carrying value of such assets can be recovered through undiscounted future operating
cash flows. If the carrying amount is not recoverable, the Company measures the amount of any impairment by comparing

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

the carrying value of the asset to the present value of the expected future cash flows associated with the use of the asset.
There have been no impairments of any long-lived assets in the periods presented.

Inventory

Inventories are stated at the lower of cost or estimated realizable value. The Company determines the cost of inventory
using  the  first-in,  first-out  (or  FIFO)  method.  The  Company  capitalizes  inventory  costs  associated  with  the  Company's
product after regulatory approval when, based on management's judgment, future commercialization is considered probable
and  the  future  economic  benefit  is  expected  to  be  realized;  otherwise,  such  costs  are  expensed  as  research  and
development.  The  Company  periodically  analyzes  its  inventory  levels  to  identify  inventory  that  may  expire  prior  to
expected  sale  or  has  a  cost  basis  in  excess  of  its  estimated  realizable  value,  and  writes-down  such  inventories  as
appropriate.  In  addition,  the  Company's  product  is  subject  to  strict  quality  control  and  monitoring  which  the  Company
performs throughout the manufacturing process. If certain batches or units of product no longer meet quality specifications
or  become  obsolete  due  to  expiration,  the  Company  records  a  charge  to  cost  of  sales  to  write  down  such  unmarketable
inventory to zero. No such charges were recorded in the years ended December 31, 2020, 2019 or 2018.

Leases

The Company determines if an arrangement is a lease at inception and records right-of-use (“ROU”) assets and lease
liabilities  on  the  consolidated  balance  sheets  at  lease  commencement  based  on  the  present  value  of  remaining  lease
payments  over  the  lease  term.  The  Company  only  considers  payments  that  are  fixed  and  determinable  at  the  time  of
commencement.

Operating lease liabilities are recognized based on the present value of the future minimum lease payments discounted
by  the  Company’s  incremental  borrowing  rate.  The  Company  measures  ROU  assets  based  on  the  corresponding  lease
liability adjusted for (i) payments made to the lessor at or before the commencement date, (ii) initial direct costs incurred
and (iii) tenant incentives under the lease. The Company’s lease terms may include options to extend or terminate the lease
when it is reasonably certain that it will exercise that option. Lease expense for minimum lease payments is recognized on
a straight-line basis over the lease term.

The Company has elected the practical expedient to exclude short-term leases from its ROU assets and lease liabilities;
therefore leases with an initial term of 12 months or less are not recorded on the balance sheet. The Company recognizes
lease expense for these leases on a straight-line basis over the lease term. The Company elected the practical expedient not
to separate non-lease components from all leases. As the Company’s leases do not provide an implicit rate, the Company
uses an incremental borrowing rate based on the information available at the lease commencement date in determining the
present  value  of  the  lease  payments.  The  Company’s  incremental  borrowing  rate  is  the  estimated  rate  that  would  be
required to pay for a collateralized borrowing equal to the total lease payment over the lease term. The Company estimates
its incremental borrowing rate based on an analysis of publicly traded debt securities of companies with credit and financial
profiles similar to its own.

For  short-term  leases,  the  Company  does  not  record  ROU  assets  or  lease  liabilities,  and  records  rent  expense  in  its
consolidated  statements  of  operations  on  a  straight-line  basis  over  the  lease  term,  with  the  exception  of  variable  lease
payments, which are expensed as incurred.

Convertible Debt

The  Company  accounts  for  convertible  debt  in  accordance  with  Financial  Accounting  Standards  Board  (“FASB”)
Accounting  Standards  Codification  Subtopic  470-20,  “Debt  with  Conversion  and  Other  Options”  (“ASC  470-20”).  The
Company  separately  accounts  for  the  liability  (debt)  and  equity  (conversion  option)  components  of  convertible  debt
instruments by allocating the proceeds from the issuance. The value assigned to the debt component is the estimated fair

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

value,  as  of  the  issuance  date,  of  a  similar  debt  instrument  without  the  conversion  option.  The  amount  of  the  equity
component  (and  resulting  debt  discount)  is  calculated  by  deducting  the  fair  value  of  the  liability  component  from  the
principal  amount  of  the  convertible  debt  instrument.  The  resulting  debt  discount  is  amortized  as  additional  non-cash
interest expense over the expected life of the notes utilizing the effective interest method. For additional information, see
Note 9 — Long-Term Debt.

Revenue Recognition

Product Revenue, Net

The  Company  recognizes  revenue  upon  shipment  of  Ocaliva  to  its  customers.  The  Company  provides  the  right  of
return to its customers for unopened product for a limited time before and after its expiration date. Returns are estimated
based on historical experience and product shelf lives.

The Company has written contracts with each of its customers that have a single performance obligation — to deliver
products  upon  receipt  of  a  customer  order  —  and  these  obligations  are  satisfied  when  delivery  occurs  and  the  customer
receives Ocaliva. The Company evaluates the creditworthiness of each of its customers to determine whether collection is
reasonably assured. The wholesale acquisition cost that the Company charges its customers for Ocaliva is adjusted to arrive
at  our  estimated  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and  discounts  related  to  Medicare,
Medicaid and other government programs, (ii) estimated costs of incentives offered to certain indirect customers including
patients, and (iii) trade allowances, such as invoice discounts for prompt payment and customer fees.

Rebates and Discounts

The Company contracts with the Centers for Medicare & Medicaid Services and other government agencies to make
Ocaliva  available  to  eligible  patients.  As  a  result,  the  Company  estimates  any  rebates  and  discounts  and  deducts  these
estimated amounts from its gross product revenues at the time the revenues are recognized. The Company’s estimates of
rebates  and  discounts  are  based  on  the  government  mandated  discounts,  which  are  statutorily-defined  and  applicable  to
these  government  funded  programs  and  assumptions  developed  using  historical  experience  with  actual  payments  and
redemptions. The Company recorded $9.5 million and $7.6 million in such estimates as of December 31, 2020 and 2019,
respectively, in accounts payable, accrued expenses and other liabilities on the consolidated balance sheets.

The  Company  contracts  with  national  authorities  in  Europe  to  make  Ocaliva  available  to  eligible  patients.  In
jurisdictions  in  which  final  pricing  is  subject  to  ongoing  negotiations  with  the  government,  the  Company  estimates  the
rebate expected to be due and deducts these estimated amounts from its gross product revenues at the time the revenues are
recognized. The Company’s estimates of such liabilities are based on current invoice pricing and total prior units sold and
assumptions  developed  using  benchmarks  of  Ocaliva  pricing  approved  in  other  relevant  European  jurisdictions.  The
Company recorded $27.4 million and $12.7 million in such estimates as of December 31, 2020 and 2019, respectively, in
accounts payable, accrued expenses and other liabilities on the consolidated balance sheets.

Other Incentives

Other  incentives  that  the  Company  offers  to  indirect  customers  include  co-pay  assistance  cards  provided  by  the
Company for PBC patients who reside in states that permit co-pay assistance programs. The Company’s co-pay assistance
program is intended to reduce each participating patient’s portion of the financial responsibility for Ocaliva purchase price
to a specified dollar amount. The Company estimates the amount of co-pay assistance provided to eligible patients based
on  the  terms  of  the  program  when  product  is  dispensed  by  the  specialty  pharmacies  to  the  patients.  These  estimates  are
based  on  redemption  information  provided  by  third-party  claims  processing  organizations.  The  Company  recorded  $1.3
million and $1.2 million in such estimates as of December 31, 2020 and 2019, respectively, in accounts payable, accrued
expenses and other liabilities on the consolidated balance sheets.

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Trade Allowances

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The Company provides invoice discounts on Ocaliva sales to certain of its customers for prompt payment and records
these discounts as a reduction to gross product revenues. These discounts are based on contractual terms. Trade allowances
are recorded in accounts receivable, net of allowance for credit losses on the consolidated balance sheets.

Licensing Revenue

The  Company  accounts  for  the  development,  regulatory  and  sales  milestones  within  an  arrangement  as  variable
consideration that is included in the transaction price only to the extent that it is probable that a significant reversal in the
amount of cumulative revenue recognized will not occur when the uncertainty associated with the variable consideration is
subsequently  resolved.  Because  the  achievement  of  the  milestones  triggering  these  payments  is  highly  susceptible  to
factors outside the entity’s influence, and the uncertainty about the amount of consideration for some of the milestones is
not expected to be resolved for a long period of time, the Company does not expect to record the associated revenue until
achievement of each milestone is imminent or has already occurred.

Research and Development Expenses

Research  and  development  costs  that  do  not  have  alternative  future  use  are  charged  to  expense  as  incurred.  This
includes the cost of conducting clinical trials, compensation and related overhead for employees and consultants involved
in research and development and the cost of the Company’s manufacturing activities to supply ongoing and future clinical
trials and preclinical studies. For periods prior to commercial launch, all manufacturing costs for OCA were expensed as
research  and  development  expenses.  The  Company  will  continue  to  incur  manufacturing  costs  for  OCA  for  other
indications such as NASH prior to their potential approval.

Stock-based Compensation

The  Company  accounts  for  stock-based  compensation  to  employees,  non-employee  directors  and  non-employees
granted  share-based  payments  for  services  in  accordance  with  ASC  Topic  718,  Compensation  —  Stock  Compensation
(“ASC 718”). The Company estimates the fair value of stock option awards using the Black-Scholes option pricing model
on  the  date  of  the  grant.  Restricted  stock  unit  awards  (“RSUs”)  and  restricted  stock  awards  (“RSAs”)  without  a  market
condition are valued based on the closing price of the Company’s common stock on the date of the grant. The fair value of
time-based stock options and RSUs is recognized and amortized on a straight-line basis over the requisite service period of
the award. Stock options granted to employees generally fully vest over four years and have a term of ten years. The fair
value of awards with market conditions is estimated using the Monte Carlo simulation method and expense is recognized
on a straight-line basis over the requisite service period of the award. The Company accounts for all forfeitures when they
occur.

Net Loss Per Share

Basic loss per share is computed by dividing net loss attributable to common stockholders (numerator) by the weighted
average  number  of  common  shares  outstanding  (denominator)  during  the  period.  Potentially  dilutive  common  shares
include the shares of common stock issuable upon the exercise of outstanding stock options and unvested restricted stock
units.  The  Company  accounts  for  the  effect  of  the  Convertible  Notes  on  diluted  net  earnings  per  share  using  the  if-
converted method as they may be settled in cash or shares at the Company’s option. Diluted net loss per share is the same
as basic net loss per share, since the effects of potentially dilutive securities are antidilutive given net losses.

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Income Taxes

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The Company utilizes the asset and liability method of accounting for income taxes. Under this method, deferred tax
assets and liabilities are determined based on the difference between the financial statement carrying amounts and tax bases
of  assets  and  liabilities  using  enacted  tax  rates  in  effect  for  years  in  which  the  temporary  differences  are  expected  to
reverse. The Company establishes a valuation allowance when it believes it is more likely than not that deferred tax assets
will not be realized.

The  Company  determines  the  need  for  a  valuation  allowance  by  assessing  the  probability  of  realizing  deferred  tax
assets,  taking  into  consideration  all  available  positive  and  negative  evidence,  including  historical  operating  results,
expectations  of  future  taxable  income,  carryforward  periods  available,  various  income  tax  strategies  and  other  relevant
factors. Judgment is required in making this assessment and to the extent future expectations change, the Company would
have to assess the recoverability of its deferred assets at that time.

The  Company’s  tax  returns  are  subject  to  examination  by  U.S.  Federal,  state,  and  foreign  taxing  jurisdictions.  The
impact  of  an  uncertain  tax  position  taken  or  expected  to  be  taken  on  an  income  tax  return  must  be  recognized  in  the
financial statements at the largest amount that is more likely than not to be sustained. An uncertain income tax position will
not be recognized in the financial statements unless it is more likely than not to be sustained.

Segments

The  Company  operates  in  one  segment  focused  on  the  development  and  commercialization  of  novel  therapeutics  to

treat progressive non-viral liver diseases.

Recently Adopted Accounting Pronouncements

In  June  2016,  the  FASB  issued  Accounting  Standards  Update  (“ASU”)  No.  2016-13,  “Financial  Instruments-Credit
Losses:  Measurement  of  Credit  Losses  on  Financial  Instruments”  (“ASU  2016-13”),  which  replaces  the  incurred  loss
impairment methodology under current U.S. GAAP with a methodology that reflects expected credit losses and requires
consideration of a broader range of reasonable and supportable information to inform credit loss estimates. ASU 2016-13
was subsequently updated by ASU No. 2019-04, “Codification Improvements to Topic 326, Financial Instruments—Credit
Losses, Topic 815, Derivatives and Hedging, and Topic 825, Financial Instruments”, to clarify that entities should include
recoveries  when  estimating  the  allowance  for  credit  losses.  The  Company  will  be  required  to  use  a  forward-looking
expected  credit  loss  model  for  accounts  receivables,  loans  and  other  financial  instruments.  Credit  losses  relating  to
available-for-sale investment debt securities will also be recorded through an allowance for credit losses rather than as a
reduction in the amortized cost basis of the securities. This guidance is effective for fiscal years, and interim periods within
those fiscal years, beginning after December 15, 2019 and must be adopted using a modified retrospective approach, with
certain  exceptions.  The  Company  adopted  ASU  2016-13  on  January  1,  2020  and  its  adoption  did  not  have  a  material
impact on the Company’s consolidated financial statements and related disclosures.

In August 2018, the FASB issued ASU No. 2018-13, “Fair Value Measurement (Topic 820): Disclosure Framework –
Changes  to  the  Disclosure  Requirements  for  Fair  Value  Measurement”  (“ASU  2018-13”),  which  makes  a  number  of
changes  meant  to  add,  modify  or  remove  certain  disclosure  requirements  associated  with  the  movement  amongst  or
hierarchy associated with Level 1, Level 2 and Level 3 fair value measurements. This guidance is effective for fiscal years,
and  interim  periods  within  those  fiscal  years,  beginning  after  December  15,  2019.  Early  adoption  is  permitted  upon
issuance of the update. The Company adopted ASU 2018-13 on January 1, 2020 and its adoption did not have any impact
on the Company’s consolidated financial statements and related disclosures.

In December 2019, the FASB issued ASU No. 2019-12, “Income Taxes (Topic 740): Simplifying the Accounting for

Income Taxes (“ASU 2019-12”), which is intended to simplify various aspects related to accounting for income

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

taxes.  ASU  2019-12  removes  certain  exceptions  to  the  general  principles  in  Topic  740  and  also  clarifies  and  amends
existing guidance to improve consistent application. This guidance is effective for fiscal years, and interim periods within
those fiscal years, beginning after December 15, 2020, with early adoption permitted. The Company adopted ASU 2019-12
on January 1, 2021 and its adoption did not have any material impact on the Company’s consolidated financial statements
and related disclosures.

Recent Accounting Pronouncements to be Adopted

In August 2020, the FASB issued ASU No. 2020-06, “Debt—Debt with Conversion and Other Options (Subtopic 470-
20)  and  Derivatives  and  Hedging—Contracts  in  Entity’s  Own  Equity  (Subtopic  815-40):  Accounting  for  Convertible
Instruments  and  Contracts  in  an  Entity’s  Own  Equity  (“ASU  2020-06”),  which  simplifies  accounting  for  convertible
instruments by removing major separation models required under current U.S. GAAP. The ASU removes certain settlement
conditions  that  are  required  for  equity  contracts  to  qualify  for  the  derivative  scope  exception  and  it  also  simplifies  the
diluted  earnings  per  share  calculation  in  certain  areas.  Either  a  modified  retrospective  method  of  transition  or  a  fully
retrospective  method  of  transition  is  permissible  for  the  adoption  of  this  standard.  This  guidance  is  effective  for  fiscal
years, and interim periods within those fiscal years, beginning after December 15, 2021, with early adoption permitted. The
Company expects the impact of this standard to be material on its consolidated financial statements and related disclosures.

3. Cash, Cash Equivalents and Investments

The following table summarizes the Company’s cash, cash equivalents and investments as of December 31, 2020 and

2019:

Cash and cash equivalents:
Cash and money market funds

Total cash and cash equivalents

Investment debt securities:
Commercial paper
Corporate debt securities

Total investment debt securities

Total cash, cash equivalents and investment debt
securities

     Amortized Cost

As of December 31, 2020

Allowance
for Credit
Losses

Gross
Unrealized
Gains

(in thousands)

Gross
Unrealized
Losses

     Fair Value

$

58,151
58,151

$

55,460
355,597
411,057

— $
—

—  
—  
—  

— $
—

— $
—

58,151
58,151

6
529
535

(9)
(67)
(76)

55,457
  356,059
  411,516

$

469,208

$

— $

535

$

(76) $ 469,667

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Cash and cash equivalents:
Cash and money market funds
Commercial paper

Total cash and cash equivalents

Investment debt securities:
Commercial paper
Corporate debt securities

Total investment debt securities

     Amortized Cost

As of December 31, 2019
Gross
Gross
Unrealized
Unrealized
Losses
Gains

(in thousands)

Fair Value

$

$

62,557
7,498
70,055

— $
—
—

— $
—
—

62,557
7,498
70,055

42,806
538,965
581,771

43
835
878

(1)
(81)
(82)

42,848
539,719
582,567

Total cash, cash equivalents and investment debt
securities

$

651,826

$

878

$

(82)

$

652,622

The  aggregate  fair  value  for  the  Company’s  available-for-sale  investment  debt  securities  that  have  been  in  an

unrealized loss position for less than twelve months or twelve months or longer is as follows:

Less than 12 months

Gross
Unrealized

As of December 31, 2020
12 months or longer
(in thousands)

Gross
Unrealized

Total

Gross
Unrealized

     Fair Value      Losses

    Fair Value     Losses

     Fair Value      Losses

Commercial paper
Corporate debt securities
Total

$ 32,970
143,076
$ 176,046

$

$

(9) $ — $ — $ 32,970
(67)
143,076
(76) $ — $ — $ 176,046

—

—

$

$

(9)
(67)
(76)

Commercial paper
Corporate debt securities
Total

Less than 12 months

Gross
Unrealized

As of December 31, 2019
12 months or longer
(in thousands)

     Gross

Unrealized

Total

     Gross

Unrealized

     Fair Value      Losses

     Fair Value     Losses

     Fair Value      Losses

$ 11,976
  121,684
$ 133,660

$

$

(1) $ — $ — $ 11,976
(81)
—   121,684
(82) $ — $ — $ 133,660

—  

$

$

(1)
(81)
(82)

At December 31, 2020, the Company had 66 available-for-sale investment debt securities in an unrealized loss position
without an allowance for credit losses. Unrealized losses on corporate debt securities have not been recognized into income
because the issuers’ bonds are of high credit quality (rated A3/A- or higher), management does not intend to sell and it is
likely that management will not be required to sell the securities prior to their anticipated recovery and the decline in fair
value  is  largely  due  to  market  conditions  and/or  changes  in  interest  rates.  The  issuers  continue  to  make  timely  interest
payments on the bonds. The fair value is expected to recover as the bonds approach maturity.

Accrued interest receivable on available-for-sale investment debt securities totaled $2.5 million at December 31, 2020,

is excluded from the estimate of credit losses and is included in Prepaid expenses and other current assets.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

4. Fair Value Measurements

The  carrying  amounts  of  the  Company’s  receivables  and  payables  approximate  their  fair  value  due  to  their  short

maturities.

Accounting principles provide guidance for using fair value to measure assets and liabilities. The guidance includes a

three-level hierarchy of valuation techniques used to measure fair value, defined as follows:

● Unadjusted Quoted Prices — The fair value of an asset or liability is based on unadjusted quoted prices

in active markets for identical assets or liabilities (Level 1).

● Pricing Models with Significant Observable Inputs — The fair value of an asset or liability is based on
information  derived  from  either  an  active  market  quoted  price,  which  may  require  further  adjustment
based on the attributes of the financial asset or liability being measured, or an inactive market transaction
(Level 2).

● Pricing  Models  with  Significant  Unobservable  Inputs  —  The  fair  value  of  an  asset  or  liability  is
primarily based on internally derived assumptions surrounding the timing and amount of expected cash
flows for the financial instrument. Therefore, these assumptions are unobservable in either an active or
inactive market (Level 3).

The Company considers an active market as one in which transactions for the asset or liability occur with sufficient
frequency  and  volume  to  provide  pricing  information  on  an  ongoing  basis.  Conversely,  the  Company  views  an  inactive
market as one in which there are few transactions for the asset or liability, the prices are not current, or price quotations
vary  substantially  either  over  time  or  among  market  makers.  Where  appropriate,  non-performance  risk,  or  that  of  a
counterparty, is considered in determining the fair values of liabilities and assets, respectively.

The  Company’s  cash  deposits  and  money  market  funds  are  classified  within  Level  1  of  the  fair  value  hierarchy
because they are valued using bank balances or quoted market prices. Investment debt securities are classified as Level 2
instruments based on market pricing and other observable inputs.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Financial assets carried at fair value are classified in the tables below in one of the three categories described above:

December 31, 2020
Assets
Cash and cash equivalents:

Money market funds

Available-for-sale investment debt securities:

Commercial paper
Corporate debt securities

Total financial assets

December 31, 2019
Assets
Cash and cash equivalents:

Money market funds
Commercial paper

Available-for-sale investment debt securities:

Commercial paper
Corporate debt securities

Total financial assets

Total

     Level 1      Level 2

     Level 3

Fair Value Measurements Using

(in thousands)

$ 15,492

$ 15,492

$

— $

55,457
  356,059
$ 427,008

—  
55,457
—   356,059
$ 411,516

$ 15,492

$

$ 19,376
7,498

$ 19,376
—

$

— $

7,498

42,848
  539,719
$ 609,441

—  
42,848
—   539,719
$ 590,065

$ 19,376

$

—

—
—
—

—
—

—
—
—

The gross realized gains and losses on sales of available-for-sale investment debt securities were immaterial for the

fiscal years ended December 31, 2020, 2019, and 2018.

The  aggregate  fair  value  of  all  available-for-sale  investment  debt  securities  (commercial  paper  and  corporate  debt

securities), by contractual maturity, are as follows:

Due in one year or less
Due after one year through two years
Total investment debt securities

Fair Value as of December 31, 

2020

2019

(in thousands)

$

$

328,077
83,439
411,516

$

$

473,602
116,463
590,065

Actual  maturities  may  differ  from  contractual  maturities  because  issuers  may  have  the  right  to  call  or  prepay

obligations without call or prepayment penalties.

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5. Fixed Assets, Net

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Fixed  assets  are  stated  at  cost  and  depreciated  or  amortized  using  the  straight-line  method  based  on  useful  lives  as

follows:

Office equipment and software
Leasehold improvements
Furniture and fixtures
Subtotal

Less: accumulated depreciation

Fixed assets, net

Useful lives
(Years)

3

  Shorter of remaining lease term or useful life

7

December 31, 

2020

2019

(in thousands)

$
5,364
  13,237
4,602
  23,203
  (16,877)
6,326
$

$

$

4,386
10,489
4,032
18,907
(13,705)
5,202

Depreciation expense for the years ended December 31, 2020, 2019 and 2018 was approximately $3.1 million, $3.7

million and $4.6 million, respectively.

6. Inventory

Inventories are stated at the lower of cost or market. Inventories consisted of the following:

December 31,

2020

2019

Work-in-process
Finished goods
Inventory

7. Leases

$

$

$

(in thousands)
8,394
633
9,027

$

8,302
160
8,462

The Company leases various office spaces under non-cancelable operating leases with original lease periods expiring
between  the  first  quarter  in  2021  and  2025.  The  Company  also  enters  into  leases  for  equipment.  A  number  of  the
Company’s leases include one or more options to renew, with renewal terms that can extend the lease term. The exercise of
lease renewal options is typically at the sole discretion of the Company; therefore, all renewals to extend the lease terms
are  not  included  in  the  ROU  assets  and  lease  liabilities  as  they  are  not  reasonably  certain  of  exercise.  The  Company
regularly evaluates the renewal options and when they are reasonably certain of exercise, includes the renewal period in the
lease term. These operating leases do not contain material variable rent payments, residual value guarantees, covenants, or
other restrictions.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Operating lease assets and liabilities are classified on the consolidated balance sheet as follows:

Leases
Assets
Operating lease assets
Total leased assets

Liabilities
Current
Operating lease liabilities

Noncurrent
Operating lease liabilities
Total operating lease liabilities

Classification

December 31, 2020 December 31, 2019

Other assets

Accounts payable, accrued expenses
and other liabilities

Long-term other liabilities

$
$

$

$

(in thousands)

12,327
12,327

$
$

13,246
13,246

7,248

$

6,456

7,684
14,932

$

9,222
15,678

Operating lease costs for the years ended December 31, 2020 and 2019, are as follows:

Lease Cost

Classification

Operating lease cost
Short-term lease cost
Variable lease cost
Sublease income
Net lease cost

Selling, general and administrative expenses
Selling, general and administrative expenses
Selling, general and administrative expenses
Other income, net

Years Ended December 31,

2020

2019

(in thousands)

6,723
3,688
1,337
(125)
11,623

$

$

6,176
2,203
829
(788)
8,420

$

$

The  weighted-average  remaining  term  of  the  Company’s  operating  leases  was  2.8  years  and  the  weighted-average
discount rate used to measure the present value of the Company’s operating lease liabilities was 5.0% as of December 31,
2020.

Cash  payments  included  in  the  measurement  of  the  Company’s  operating  lease  liabilities  reported  in  operating  cash
flows were $7.9 million and $7.5 million for the years ended December 31, 2020 and 2019, respectively. During the year
ended  December  31,  2020,  the  Company  obtained  ROU  assets  of  $4.7  million  in  exchange  for  new  operating  lease
obligations of $6.1 million.

F-23

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Maturities  of  the  Company’s  operating  lease  liabilities,  which  do  not  include  short-term  leases,  as  of  December  31,

2020 are as follows:

Maturity of Lease Liabilities

2021
2022
2023
2024
2025
Thereafter
Total lease payments
Less: Present value discount
Total operating lease liabilities

Operating leases

(in thousands)

7,875
3,632
2,141
1,612
1,033
—
16,293
(1,361)
14,932

$

$

8. Accounts Payable, Accrued Expenses and Other Liabilities

Accounts payable, accrued expenses and other liabilities consisted of the following:

Accounts payable
Accrued employee compensation
Accrued contracted services
Accrued restructuring
Accrued rebates, discounts and other incentives
Operating lease liabilities
Other liabilities
Accounts payable, accrued expenses and other liabilities

Research & Development Tax Credit

2020

December 31, 

(in thousands)

2019

$

$

24,594
27,154
62,425
2,504
38,172
7,248
8,942
171,039

$

$

18,975
26,483
74,486
—
21,529
6,456
6,039
153,968

The Company has benefited from the U.K. Small and Medium-sized Enterprise R&D Tax Credit scheme, or the SME
scheme, under which it can obtain a tax credit of up to 33.4% of eligible research and development expenses incurred by
the Company in the U.K. Eligible expenses generally include employment costs for research staff, consumables, software
and certain internal overhead costs incurred as part of research projects.

The Company has submitted claims seeking to obtain tax credits for qualifying R&D expenses incurred in the 2015,
2016, and 2017 calendar years. As described further in Note 14, the 2015 and 2016 claim was finalized during the quarter
ended June 30, 2020, and therefore the $10.5 million payment received in September 2019, which was previously deferred,
was released into income.

With respect to the 2017 claim, in June 2020, the Company received a payment of $9.4 million from Her Majesty’s
Revenue and Customs (“HMRC”), the U.K.’s government tax authority. Given the claim review has not been finalized for
the  2017  year,  the  $9.4  million  credit  payment  received  along  with  an  additional  $1.0  million  due  to  foreign  currency
translation are recorded as a deferred liability within Accounts payable, accrued expenses and other liabilities.

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9. Long-Term Debt

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Debt, net of discounts and deferred financing costs, consisted of the following:

2023 Convertible Notes
2026 Convertible Notes
Long-term debt, gross

Less: Unamortized debt discounts and fees

Long-term debt, net

2019 Offering

December 31,

2020

2019

(in thousands)

$

$

460,000
230,000
690,000
(129,418)
560,582

$

$

460,000
230,000
690,000
(157,922)
532,078

On  May  14,  2019,  the  Company  issued  and  sold  $230.0  million  aggregate  principal  amount  of  2.00%  Convertible
Senior  Notes  due  2026  (the  “2026  Convertible  Notes”).  The  Company  received  net  proceeds  from  the  sale  of  the  2026
Convertible Notes of $223.4 million, after deducting underwriting discounts, commissions and estimated offering expenses
of approximately $6.6 million.

The 2026 Convertible Notes were issued pursuant to a Second Supplemental Indenture, dated as of May 14, 2019 (the
“Second Supplemental Indenture”), which supplements the Indenture (the “Base Indenture”), as supplemented by a First
Supplemental  Indenture  (the  “First  Supplemental  Indenture”  and  collectively  with  the  Base  Indenture  and  the  Second
Supplemental  Indenture,  the  “Indenture”),  each  dated  as  of  July  6,  2016,  by  and  between  the  Company  and  U.S.  Bank
National  Association,  as  trustee.  The  2026  Convertible  Notes  are  senior  unsecured  obligations  of  the  Company,  bear
interest at a fixed rate of 2.00% per annum (payable semi-annually on May 15 and November 15 of each year, beginning
on November 15, 2019) and will mature on May 15, 2026, unless earlier repurchased, redeemed or converted. Holders may
convert  their  2026  Convertible  Notes  at  their  option  at  any  time  prior  to  the  close  of  business  on  the  business  day
immediately  preceding  February  15,  2026  only  under  the  following  circumstances:  (i)  during  any  calendar  quarter  (and
only during such calendar quarter) commencing after the calendar quarter ended on June 30, 2019, if the last reported sale
price  of  the  Company’s  common  stock  for  at  least  20  trading  days  (whether  or  not  consecutive)  during  a  period  of  30
consecutive trading days ending on the last trading day of the immediately preceding calendar quarter is greater than or
equal to 130% of the conversion price on each applicable trading day; (ii) during the five business day period after any five
consecutive trading day period in which the trading price (as defined in the Indenture) per $1,000 principal amount of 2026
Convertible Notes for each trading day of such five consecutive trading day period was less than 98% of the product of the
last  reported  sale  price  of  the  Company’s  common  stock  and  the  conversion  rate  on  each  such  trading  day;  (iii)  if  the
Company calls any or all of the 2026 Convertible Notes for redemption, at any time prior to the close of business on the
scheduled  trading  day  immediately  preceding  the  redemption  date;  or  (iv)  upon  the  occurrence  of  specified  corporate
events. On or after February 15, 2026 until the close of business on the business day immediately preceding the maturity
date,  holders  may  convert  their  2026  Convertible  Notes  at  any  time,  regardless  of  the  foregoing  circumstances.  Upon
conversion  of  the  2026  Convertible  Notes,  the  Company  will  pay  or  deliver,  as  the  case  may  be,  cash,  shares  of  the
Company’s common stock (and cash in lieu of any fractional shares) or a combination of cash and shares of the Company’s
common stock, at the Company’s election. The initial conversion rate of the 2026 Convertible Notes is 9.2123 shares of the
Company’s  common  stock  per  $1,000  principal  amount  of  2026  Convertible  Notes,  which  is  equivalent  to  an  initial
conversion price of approximately $108.55 per share of the Company’s common stock. The conversion rate is subject to
adjustment  in  some  events  but  will  not  be  adjusted  for  any  accrued  and  unpaid  interest.  In  addition,  following  certain
corporate  events  that  occur  prior  to  the  maturity  date,  the  Company  will  increase  the  conversion  rate  for  a  holder  who
elects  to  convert  its  2026  Convertible  Notes  in  connection  with  such  a  corporate  event  in  certain  circumstances.  The
Company may not redeem the 2026 Convertible Notes prior to May 20, 2023. The Company may redeem for cash all or
any portion of the 2026 Convertible Notes, at the Company’s option, on or after May 20, 2023, if the last reported sale

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NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

price of the Company’s common stock has been at least 130% of the conversion price then in effect for at least 20 trading
days  (whether  or  not  consecutive)  during  any  30  consecutive  trading  day  period  (including  the  last  trading  day  of  such
period) ending on, and including, the trading day immediately preceding the date on which the Company provides notice of
redemption at a redemption price equal to 100% of the principal amount of the 2026 Convertible Notes to be redeemed,
plus  accrued  and  unpaid  interest  to,  but  excluding,  the  redemption  date.  No  sinking  fund  is  provided  for  the  2026
Convertible Notes. If the Company undergoes a fundamental change (as defined in the Indenture), holders may require the
Company to repurchase for cash all or any portion of their 2026 Convertible Notes at a fundamental change repurchase
price  equal  to  100%  of  the  principal  amount  of  the  2026  Convertible  Notes  to  be  repurchased,  plus  accrued  and  unpaid
interest to, but excluding, the fundamental change repurchase date. The Indenture provides for customary events of default.

In  accordance  with  ASC  470-20,  the  Company  used  an  effective  interest  rate  of  9.9%  to  determine  the  liability
component of the 2026 Convertible Notes. This resulted in the recognition of $137.5 million as the liability component of
the  2026  Convertible  Notes  and  the  recognition  of  the  residual  $85.9  million  as  the  debt  discount  with  a  corresponding
increase to additional paid-in capital for the equity component of the 2026 Convertible Notes. The underwriting discount
and  estimated  offering  expenses  totaling  $6.6  million  were  allocated  between  the  debt  and  equity  issuance  costs  in
proportion  to  the  allocation  of  the  liability  and  equity  components  of  the  2026  Convertible  Notes.  Accordingly,  equity
issuance costs of $2.5 million were recorded as an offset to additional paid-in capital and total debt issuance costs of $4.1
million were recorded on the issuance date and are reflected in the consolidated balance sheet as a direct deduction from
the carrying value of the associated debt liability. The debt discount and debt issuance costs will be amortized as non-cash
interest expense through May 15, 2026.

The fair value of the 2026 Convertible Notes was approximately $142.8 million and $294.9 million at December 31,

2020 and December 31, 2019, respectively, and was determined using Level 2 inputs based on quoted market values.

2016 Offerings

On July 6, 2016, the Company issued and sold $460.0 million aggregate principal amount of 3.25% Convertible Senior
Notes due 2023 (the “2023 Convertible Notes”, and together with the 2026 Convertible Notes, the “Convertible Notes”).
The  Company  received  net  proceeds  from  the  sale  of  the  2023  Convertible  Notes  of  $447.6  million,  after  deducting
underwriting discounts, commissions and estimated offering expenses of approximately $12.4 million. The Company used
approximately $38.4 million of such net proceeds to fund the cost of the Capped Call Transactions (as defined below) that
were entered into in connection with the issuance of the 2023 Convertible Notes.

The 2023 Convertible Notes were issued pursuant to the Base Indenture, as supplemented by the First Supplemental
Indenture. The 2023 Convertible Notes are senior unsecured obligations of the Company, bear interest at a fixed rate of
3.25%  per  year  (payable  semi-annually  on  January  1  and  July  1  of  each  year,  beginning  on  January  1,  2017)  and
will  mature  on  July  1,  2023,  unless  earlier  repurchased,  redeemed  or  converted.  Holders  may  convert  their  2023
Convertible  Notes  at  their  option  at  any  time  prior  to  the  close  of  business  on  the  business  day  immediately  preceding
January  1,  2023  only  under  the  following  circumstances:  (i)  during  any  calendar  quarter  commencing  after  the  calendar
quarter ended on September 30, 2016, if the last reported sale price of the Company’s common stock for at least 20 trading
days (whether or not consecutive) during the period of 30 consecutive trading days ending on the last trading day of the
immediately preceding calendar quarter is greater than or equal to 130% of the conversion price on each applicable trading
day; (ii) during the five business day period after any five consecutive trading day period in which the trading price (as
defined  in  the  Indenture)  per  $1,000  principal  amount  of  2023  Convertible  Notes  for  each  trading  day  of  such  five
consecutive trading day period was less than 98% of the product of the last reported sale price of the Company’s common
stock and the conversion rate on each such trading day; (iii) if the Company calls any or all of the 2023 Convertible Notes
for  redemption,  at  any  time  prior  to  the  close  of  business  on  the  scheduled  trading  day  immediately  preceding  the
redemption date; or (iv) upon the occurrence of specified corporate events. On or after January 1, 2023 until the close of
business  on  the  second  scheduled  trading  day  immediately  preceding  the  maturity  date,  holders  may  convert  their  2023
Convertible Notes at any time, regardless of the foregoing circumstances. Upon conversion of the 2023 Convertible Notes,

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

the Company will pay or deliver, as the case may be, cash, shares of the Company’s common stock (and cash in lieu of any
fractional shares) or a combination of cash and shares of the Company’s common stock, at the Company’s election. The
initial  conversion  rate  of  the  2023  Convertible  Notes  is  5.0358  shares  of  the  Company’s  common  stock  per  $1,000
principal amount of 2023 Convertible Notes, which is equivalent to an initial conversion price of approximately $198.58
per  share  of  the  Company’s  common  stock.  The  conversion  rate  is  subject  to  adjustment  upon  the  occurrence  of  certain
events but will not be adjusted for any accrued and unpaid interest. If the Company undergoes a fundamental change (as
defined  in  the  Indenture),  holders  may  require  the  Company  to  repurchase  for  cash  all  or  any  portion  of  their  2023
Convertible  Notes  at  a  fundamental  change  repurchase  price  equal  to  100%  of  the  principal  amount  of  the  2023
Convertible  Notes  to  be  repurchased,  plus  accrued  and  unpaid  interest  to,  but  excluding,  the  fundamental  change
repurchase  date.  In  addition,  if  certain  make-whole  fundamental  changes  occur,  the  Company  will,  in  certain
circumstances, increase the conversion rate for any 2023 Convertible Notes converted in connection with such make-whole
fundamental change. The Company may not redeem the 2023 Convertible Notes prior to July 6, 2021. The Company may
redeem for cash all or part of the 2023 Convertible Notes, at its option, on or after July 6, 2021, if the last reported sale
price of the Company’s common stock has been at least 130% of the conversion price then in effect for at least 20 trading
days  (whether  or  not  consecutive)  during  any  30  consecutive  trading  day  period  (including  the  last  trading  day  of  such
period) ending on, and including, the trading day immediately preceding the date on which the Company provides notice of
redemption at a redemption price equal to 100% of the principal amount of the 2023 Convertible Notes to be redeemed,
plus accrued and unpaid interest to, but excluding, the redemption date. The Indenture provides for customary events of
default.

On  June  30,  2016,  in  connection  with  the  pricing  of  the  2023  Convertible  Notes,  the  Company  entered  into  privately-
negotiated capped call transactions (the “Base Capped Call Transactions”) with each of Royal Bank of Canada, UBS AG,
London  Branch,  and  Credit  Suisse  Capital  LLC  (the  “Option  Counterparties”).  On  July  1,  2016,  in  connection  with  the
underwriters’ exercise of their over-allotment option in full, the Company entered into additional capped call transactions
(the  “Additional  Capped  Call  Transactions”  and,  together  with  the  Base  Capped  Call  Transactions,  the  “Capped  Call
Transactions”)  with  the  Option  Counterparties.  The  Capped  Call  Transactions  are  expected  generally  to  reduce  the
potential dilution with respect to the Company’s common stock and/or offset the cash payments the Company would be
required  to  make  in  excess  of  the  principal  amount  of  converted  2023  Convertible  Notes,  as  the  case  may  be,  upon
conversion of the 2023 Convertible Notes in the event that the market price per share of the Company’s common stock, as
measured under the terms of the Capped Call Transactions, is greater than the strike price of the Capped Call Transactions,
which  initially  corresponds  to  the  conversion  price  of  the  2023  Convertible  Notes  and  is  subject  to  anti-dilution
adjustments substantially similar to those applicable to the conversion rate of the 2023 Convertible Notes. The cap price of
the Capped Call Transactions is initially $262.2725 per share, and is subject to certain adjustments under the terms of the
Capped Call Transactions. If, however, the market price per share of the Company’s common stock, as measured under the
terms of the Capped Call Transactions, exceeds the cap price of the Capped Call Transactions, there would nevertheless be
dilution  and/or  there  would  not  be  an  offset  of  such  potential  cash  payments,  in  each  case,  upon  conversion  of  the
Convertible Notes to the extent that such market price exceeds the cap price of the Capped Call Transactions. The Capped
Call  Transactions  are  considered  to  be  instruments  indexed  to  the  Company’s  own  shares  and  met  the  criteria  to  be
classified within equity and are therefore not remeasured.

In  accordance  with  ASC  470-20,  the  Company  used  an  effective  interest  rate  of  8.4%  to  determine  the  liability
component of the 2023 Convertible Notes. This resulted in the recognition of $334.4 million as the liability component of
the 2023 Convertible Notes and the recognition of the residual $113.1 million as the debt discount with a corresponding
increase to additional paid-in capital for the equity component of the 2023 Convertible Notes.

The fair value of the 2023 Convertible Notes was approximately $363.7 million and $463.5 million at December 31,

2020 and December 31, 2019, respectively, and was determined using Level 2 inputs based on quoted market values.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Interest Expense on Convertible Notes

The table summarizes the total interest expense recognized in the periods presented:

Contractual interest expense
Amortization of debt discount
Amortization of debt issuance costs
Total interest expense

2020

Years Ended December 31, 
2019
(in thousands)

2018

$

$

19,550
25,964
2,540
48,054

$

$

17,825
21,189
2,130
41,144

$

$

14,950
14,032
1,541
30,523

Accrued interest on the Convertible Notes was approximately $8.1 million and $8.1 million as of December 31, 2020
and 2019, respectively. The Company recorded debt issuance costs of $19.0 million, which are being amortized using the
effective  interest  method.  As  of  December  31,  2020,  and  2019,  $10.7  million  and  $13.2  million,  respectively,  of  debt
issuance costs are recorded on the consolidated balance sheets in Long-term debt. Cash payments for interest were $19.6
million and $17.3 million for the years ended December 31, 2020 and 2019, respectively.

10. Stockholders’ Equity and Preferred Stock

Increase in Authorized Shares of Common Stock

On May 28, 2020, at the 2020 Annual Meeting of Stockholders, the Company obtained approval from its stockholders
to increase the number of authorized shares of the Company’s common stock, par value $0.001, from 45,000,000 shares to
90,000,000  shares.  The  increase  in  the  authorized  shares  of  common  stock  was  effectuated  pursuant  to  a  Certificate  of
Amendment  to  the  Company’s  restated  certificate  of  incorporation,  filed  with  the  Secretary  of  the  State  of  Delaware  on
May 28, 2020.

2019 Public Offering and Concurrent Private Placement

On May 14, 2019, the Company issued and sold (i) 2,760,000 shares of common stock in a registered public offering
(including  360,000  shares  issued  and  sold  upon  the  exercise  in  full  of  the  underwriters’  option  to  purchase  additional
shares), at a price to the public of $83.50 per share (the “2019 Public Offering”) and (ii) 119,760 shares of common stock
(the “2019 Private Placement Shares”) in a concurrent private placement of common stock (the “2019 Concurrent Private
Placement”) exempt from the registration requirements of the Securities Act of 1933, as amended (the “Securities Act”), at
a purchase price per share equivalent to the price to the public set in the 2019 Public Offering and pursuant to a securities
purchase agreement (the “2019 Securities Purchase Agreement”) that the Company entered into with Samsara BioCapital,
L.P. (“Samsara”), one of the Company’s existing stockholders. Pursuant to the 2019 Securities Purchase Agreement, the
Company granted to Samsara certain registration rights requiring the Company, upon request of Samsara on or after July 9,
2019 and subject to certain terms and conditions, to register the resale by Samsara of its 2019 Private Placement Shares.
Such registration rights have since expired.

Common Stock

As of December 31, 2020 and 2019, the Company had 90,000,000 and 45,000,000 authorized shares of common stock,

par value $0.001 per share, respectively.

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Dividends

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Subject to preferences that may be applicable to any outstanding shares of preferred stock, holders of common stock
are  entitled  to  receive  ratably  such  dividends,  if  any,  as  may  be  declared  from  time  to  time  by  the  Company’s  board  of
directors out of funds legally available for dividend payments. The Company has never declared or paid any cash dividends
on its common stock, and does not anticipate paying any cash dividends on its common stock in the foreseeable future. The
Company  intends  to  retain  all  available  funds  and  any  future  earnings  to  fund  the  development  and  expansion  of  its
business. Any future determination to pay dividends will be at the discretion of the board of directors and will depend upon
a  number  of  factors,  including  the  results  of  operations,  financial  condition,  future  prospects,  contractual  restrictions,
restrictions imposed by applicable law and other factors the board of directors deems relevant.

Voting

Holders of common stock are entitled to one vote for each share held with respect to all matters submitted to a

vote of the stockholders and do not have cumulative voting rights.

Preferred Stock

As  of  December  31,  2020  and  2019,  the  Company  had  5,000,000  authorized  shares  of  preferred  stock,  par  value

$0.001 per share, of which none are issued.

11. Product Revenue, Net

The  Company  recognized  net  sales  of  Ocaliva  of  $312.7  million,  $249.6  million  and  $177.8  million  for  the  years

ended December 31, 2020, 2019 and 2018, respectively.

The table below summarizes consolidated product revenue, net by region:

2020

Years Ended December 31, 
2019
(in thousands)

2018

$

$

233,970
78,720
312,690

$

$

187,436
62,134
249,570

$

$

140,822
36,960
177,782

Product revenue, net:

U.S.
ex-U.S.

Total product revenue, net

12. License Agreement

Sumitomo Dainippon Pharma Co., Ltd.

In  March  2011,  the  Company  entered  into  an  exclusive  license  agreement  (the  “Sumitomo  Agreement”)  with
Sumitomo Dainippon Pharma Co., Ltd. (“Sumitomo Dainippon”), pursuant to which the Company granted to Sumitomo
Dainippon an exclusive license to research, develop and commercialize OCA for the treatment of PBC and NASH in Japan
and China (excluding Taiwan) and an option to research, develop and commercialize OCA in certain countries outside of
such territories (the “Country Option”). The Company received an upfront payment from Sumitomo Dainippon of $15.0
million under the terms of the Sumitomo Agreement. In October 2019, the Company and Sumitomo Dainippon mutually
agreed to terminate with immediate effect the Sumitomo Agreement. In connection with the termination of the Sumitomo
Agreement, Sumitomo Dainippon agreed to return to the Company the rights to develop and commercialize OCA in China
and the Company agreed to forego any further milestone or royalty payments relating to the development and

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

commercialization of OCA in China. No payment was due from the Company to Sumitomo Dainippon as a result of the
termination of the Sumitomo Agreement.

The Company recognized licensing revenue of approximately $0, $2.4 million and $2.0 million for the years ended

December 31, 2020, 2019, and 2018, respectively, under the Sumitomo Agreement.

13. Stock Compensation

The  Company’s  2012  Equity  Incentive  Plan  (“2012  Plan”)  became  effective  upon  the  pricing  of  its  initial  public
offering  in  October  2012  (the  “IPO”).  At  the  same  time,  the  Company’s  2003  Stock  Incentive  Plan  (“2003  Plan”)  was
terminated and 555,843 shares available under the 2003 Plan were added to the 2012 Plan.

On January 1, 2020, the number of shares available for issuance under the 2012 Plan increased by 1,211,533 as a result

of the automatic increase provisions thereof.

The estimated fair value of the stock options granted in the year ended December 31, 2020 was determined utilizing a
Black-Scholes option-pricing model at the date of grant. The fair value of the RSUs granted in the year ended December
31, 2020 was determined utilizing the closing price of the Company’s common stock on the date of grant. The fair value of
the performance restricted stock units (“PRSUs”) granted in the year ended December 31, 2020 was determined utilizing
the  Monte  Carlo  simulation  method.  The  Company  accounts  for  all  forfeitures  when  they  occur.  Ultimately,  the  actual
expense recognized over the vesting period will be for only those shares that vest and are not forfeited.

The Company has in the past, and may in the future, grant performance-based awards with vesting terms based on the
achievement of specified goals. To the extent such awards do not contain a market condition, the Company recognizes no
expense  until  achievement  of  the  performance  requirement  is  deemed  probable.  There  are  no  option  awards  with
performance conditions outstanding as of December 31, 2020.

There  were  approximately  3.3  million  and  2.8  million  shares  available  for  grant  remaining  under  the  2012  Plan  at

December 31, 2020 and 2019, respectively.

Stock Options and Performance-Based Stock Options

The  Company’s  outstanding  option  activity  for  the  period  from  December  31,  2019  through  December  31,  2020  is

summarized as follows:

Outstanding at December 31, 2019
Granted
Exercised
Cancelled/forfeited
Expired
Outstanding at December 31, 2020
Expected to vest
Exercisable

Number
of Options
(in thousands)

Weighted
Average

Weighted
Average
Remaining
Contractual

Exercise Price      Term (years)     

Aggregate
Intrinsic Value
(in thousands)

1,981
727
(22)
(368)
(119)
2,199
779
1,420

$
$
$
$
$
$
$
$

99.87  
90.03  
52.20  
91.18  
130.35  
96.92  
86.35  
102.73  

$
7.4
— $
— $
— $
— $
$
6.9
$
8.3
$
6.1

65,662
—
—
—
—
146
—
146

The  aggregate  intrinsic  value  of  options  is  calculated  as  the  difference  between  the  exercise  price  of  the  underlying

options and the deemed fair value of the Company’s common stock for those options that had exercise prices lower than

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

the deemed fair value of the Company’s common stock. The weighted-average grant date fair value of options granted in
the years ended December 31, 2020, 2019 and 2018 was $52.48, $74.78 and $41.18 per option, respectively. The aggregate
intrinsic  value  of  stock  options  exercised  during  the  years  ended  December  31,  2020,  2019  and  2018  was  $0.9  million,
$10.2 million and $14.1 million, respectively. As of December 31, 2020, the total compensation cost related to non-vested
option awards not yet recognized is approximately $34.1 million with a weighted average remaining vesting period of 1.20
years.

The  Company  estimated  the  fair  value  of  stock  options  granted  in  the  periods  presented  utilizing  a  Black-Scholes

option-pricing model utilizing the following assumptions:

Volatility
Expected term (in years)
Risk-free rate
Expected dividend yield

Years Ended December 31, 

2020

2019

2018

  61.9 - 87.1 % 86.9 - 89.9 % 62 - 73 %

5.5 - 6.0  
0.2 - 1.7 %  
— %  

6.0

5.5 - 6.0  
1.4 - 2.9 % 1.8 - 3.0 %
— %

— %

In  April  2014,  the  Company  issued  57,063  performance-based  options  to  certain  employees  that  will  vest  upon  the
achievement of certain regulatory milestones related to OCA at future dates. In November 2014, the Company issued an
additional 10,839 performance-based options that will vest upon the achievement of the same regulatory milestones. As of
December 31, 2020, the achievement of such milestones was not met and these performance-based options were cancelled.

Restricted Stock Units and Awards & Performance-Based Restricted Stock Units and Awards

The following table summarizes the aggregate RSU, RSA, PRSU and performance restricted share award (“PRSA”)

activity for the year ended December 31, 2020:

Non-vested awards at December 31, 2019

Granted
Vested
Forfeited

Non-vested awards at December 31, 2020

Number of
Awards
(in thousands)
$
709
725
$
(374) $
(261) $
799
$

Weighted
Average Grant Date
Fair Value

88.39
74.68
85.06
89.37
72.43

For the years ended December 31, 2020, 2019 and 2018, the weighted-average grant date fair value of RSUs, RSAs,
PRSUs and PRSAs granted was $74.68, $107.29 and $65.28, respectively. The total fair value of RSUs, RSAs, PRSUs and
PRSAs that vested during the years ended December 31, 2020, 2019 and 2018 was $30.7 million, $29.8 million and $24.0
million, respectively. As of December 31, 2020, there was $45.5 million of unrecognized compensation expense related to
unvested RSUs, RSAs, PRSUs, and PRSAs, which is expected to be recognized over a weighted average period of 1.31
years.

During  the  years  ended  December  31,  2020,  2019  and  2018,  the  Company  granted  a  total  of  64,900,  57,800  and
51,200 PRSUs to certain of the Company’s executive officers. During the year ended December 31, 2018, the Company
granted a total of 4,300 PRSAs to certain of the Company’s executive officers. The performance criterion for such PRSUs
and PRSAs is based on the Total Shareholder Return (“TSR”) of the Company’s common stock relative to the TSR of the
companies comprising the S&P Biotechnology Select Industry Index (the “TSR Peer Group”) over a 3-year performance
period and is accounted for as a market condition under ASC 718. The TSR for the Company or a member of the TSR

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Peer Group is calculated by dividing (a) the difference of the ending average stock price minus the beginning average stock
price by (b) the beginning average stock price. The beginning average stock price equals the average closing stock price
over  the  one  calendar  month  period  prior  to  the  beginning  of  the  performance  period,  after  adjusting  for  dividends,  as
applicable. The ending average stock price equals the average closing price over the one calendar month period ending on
the last day of the performance period, after adjusting for dividends, as applicable. The Company’s relative TSR is then
used to calculate the payout percentage, which may range from zero percent (0%) to one hundred and fifty percent (150%)
of the target award. The Company utilized a Monte Carlo Simulation to determine the grant date fair value of such PRSUs
and  PRSAs.  The  Company  recorded  approximately  $8.0  million  (of  which  $2.9  million  related  to  modifications),  $4.0
million  and  $1.3  of  stock-based  compensation  related  to  such  PRSUs  and  PRSAs  during  the  years  ended  December  31,
2020, 2019 and 2018, respectively.

Stock-based compensation expense has been reported in the Company’s statements of operations as follows:

Selling, general and administrative
Research and development
Restructuring
Total stock-based compensation

14. Research and Development Tax Credit

$

$

Years Ended December 31, 
2019
(in thousands)
$

$

43,170
12,812
—
55,982

$

$

2020

45,985
12,824
2,041
60,850

2018

38,361
11,553
—
49,914

The Company has benefited from the U.K. Small and Medium-sized Enterprise R&D Tax Credit scheme, or the SME
scheme, under which it can obtain a tax credit of up to 33.4% of eligible research and development expenses incurred by
the Company in the U.K. Eligible expenses generally include employment costs for research staff, consumables, software
and certain internal overhead costs incurred as part of research projects.

The Company submitted a claim seeking to obtain tax credits for qualifying R&D expenses incurred in the years ended
December 31, 2015 and 2016. In September 2019, the Company received a partial payment of $10.5 million from HMRC.
In April 2020, the Company received the remaining payment for the 2015 and 2016 claim years of $11.3 million.

The  claim  for  2015  and  2016  was  finalized  and  approved  in  the  quarter  ended  June  30,  2020,  at  which  time  the
Company  recorded  the  U.K.  research  and  development  tax  credit  payments  received  of  $22.0  million  as  a  reduction  of
research and development expense in the consolidated statements of operations.

15. Employee Benefit Plans

The Company maintains a defined contribution plan, which is qualified under section 401(k) of the Internal Revenue
Code for U.S. employees. Employees may make contributions by withholding a percentage of their salary up to the Internal
Revenue Service annual limit of $19,500 and $26,000 in 2020 for employees under 50 years old and employees 50 years
old or over, respectively. The Company’s matching contribution vests over four years from the start of employment. The
Company made approximately $2.2 million, $1.4 million and $1.9 million in matching contributions for the years ended
December 31, 2020, 2019 and 2018, respectively.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

16. Restructuring Expenses

On August 31, 2020, the Company adopted a plan to reduce its workforce in light of the previously announced receipt
of  a  complete  response  letter  from  the  U.S.  Food  and  Drug  Administration  (the  “FDA”)  with  respect  to  its  New  Drug
Application for OCA for the treatment of liver fibrosis due to NASH (the “2020 Workforce Plan”). The 2020 Workforce
Plan  sought  to  streamline  the  Company’s  operations  and  reduce  operating  expenses,  while  maintaining  the  critical
resources  needed  to  continue  to  support  the  NASH  and  PBC  clinical  programs,  pursue  the  approval  of  OCA  for  the
treatment of liver fibrosis due to NASH and support the Company’s successful PBC business. The 2020 Workforce Plan
resulted in a workforce reduction of approximately 25%, or approximately 170 employees. The 2020 Workforce Plan was
implemented during the third quarter of 2020, immediately after its announcement, was substantially completed by the end
of  2020  with  expected  completion  by  the  end  of  2021  upon  payments  of  cash  for  charges  incurred  under  the  2020
Workforce Plan. In the year ended December 31, 2020 the Company recorded restructuring charges of $14.6 million, which
were  primarily  related  to  severance  costs  and  other  related  termination  benefits  incurred  in  conjunction  with  the  2020
Workforce Plan.

The  following  table  reflects  total  expenses  related  to  restructuring  activities  recognized  within  the  Consolidated

Statements of Operations as restructuring costs:

Employee compensation costs
Equity compensation costs
Total restructuring costs

2020

Years Ended December 31, 
2019
(in thousands)

2018

$

$

12,589  
2,041
14,630

$

$

—
—
—

$

$

—
—
—

The  Company  recorded  $2.0  million  in  non-cash  stock-based  compensation  expense  in  association  with  the

acceleration of the vesting of certain options and RSUs held by terminated employees.

The following table displays a rollforward of the changes to the accrued balances as of December 31, 2020:

Accrued balance at December 31, 2019
Charges incurred
Cash payments made
Other reserve adjustments
Accrued balance at December 31, 2020

Severance and Related Costs

(in thousands)

—
13,544
(10,068)
(972)
2,504

$

$

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17. Income Taxes

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  components  of  loss  before  income  taxes  for  the  years  ended  December  31,  2020,  2019  and  2018  includes  the

following:

United States
Foreign
Total

2020

Years Ended December 31, 
2019
(in thousands)
$ (126,351) $ (95,708) $ (72,655)
  (148,529)
  (236,587)
  (248,973)
$ (274,880) $ (344,681) $ (309,242)

2018

Income tax expense (benefit) differed from the amounts computed by applying the statutory U.S. Federal income tax

rate of 21% to loss before income taxes as a result of the following:

Computed "expected" tax benefit
State taxes, net of U.S. Federal benefit
U.S. Federal tax credits
U.S. Federal valuation allowance
Stock-based compensation
Officer compensation
Foreign valuation allowance
Foreign tax rate differences
Other
Total

F-34

2018

2020

—
—  

Years Ended December 31, 
2019
(in thousands)
$ (57,725) $ (72,383) $ (64,941)
—
—
9,352
6,423
22
44,896
4,787
(539)
—

14,786
4,609
508
19,349
32,936
195
— $

—
(5,787)
26,279
8,098
437
43,414
(12,223)
(2,493)

— $

$

    
    
    
    
    
    
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The tax effects of temporary differences that give rise to the deferred tax assets and liabilities at December 31, 2020

and 2019 are presented below:

Deferred tax assets:

U.S. and state net operating loss and other carryforwards
Foreign net operating loss and other carryforwards
Stock compensation
Accrued compensation
Accrued expense
Intangible property
Interest limitation
Other

Deferred tax assets before valuation allowance
Valuation allowance
Total deferred tax assets
Deferred tax liabilities:
Convertible Notes

Total deferred tax liabilities
Net deferred tax asset (liability)

December 31, 

2020

2019

(in thousands)

$

$

178,007
239,607
15,675
5,042
11,143
1,945
9,419
1,749
462,587
(436,476)
26,111

(26,111)
(26,111)

$

— $

160,079
195,590
13,626
4,997
1,750
2,088
5,183
1,406
384,719
(353,677)
31,042

(31,042)
(31,042)
—

Effects of the Coronavirus Aid, Relief and Economic Security Act

On March 27, 2020, the United States enacted the Coronavirus Aid, Relief and Economic Security Act (the “CARES
Act”).  The  CARES  Act,  among  other  things,  made  changes  to  NOLS  rules,  including  the  allowance  of  a  five-year
carryback  period  for  NOLs  arising  in  tax  years  beginning  after  December  31,  2017  and  before  January  1,  2021  and
removed  the  80%  taxable  income  limitation  for  NOL  deductions  for  tax  years  beginning  before  January  1,  2021.  The
enactment of the CARES Act did not result in any material adjustments to the Company’s provision for income taxes.

Net Operating Loss and other carryforwards

As of December 31, 2020, and 2019, the Company had net operating loss carryforwards (“NOLs”) for U.S. Federal
income tax purposes of $709.4 million and $693.3 million, respectively, and other carryforwards of $13.7 million and $0.5
million, respectively. The enactment of the Tax Cuts and Jobs Act (“TCJA”) modified the ability of companies to utilize
NOLs  arising  in  tax  years  beginning  on  or  after  January  1,  2018  by  providing  that  such  NOLs  may  be  carried-forward
indefinitely and used to offset up to 80 percent of taxable income in any given future year. Existing NOLs that arose in tax
years beginning prior to January 1, 2018 were not affected by the TCJA and are generally eligible to be carried-forward for
up to 20 years and used to fully offset taxable income in future years. If not utilized, the Company’s pre-2018 NOLs and
other  carryforwards  will  expire  for  U.S.  Federal  income  tax  purposes  between  2024  and  2037.  The  Company  also  has
certain state NOLs in varying amounts depending on the different state tax laws.

As of December 31, 2020, and 2019, the Company had NOLs for foreign income tax purposes of $1.2 billion and $1.1
billion,  respectively.  Of  our  $1.2  billion  of  foreign  tax  loss  carryforwards,  approximately  $1.1  billion  may  be  carried
forward indefinitely and the remainder will expire during the next 17 years.

In addition, the Company’s ability to utilize its NOLs may be limited under Section 382 of the Internal Revenue Code
or applicable state and foreign tax law. The Section 382 limitations apply if an “ownership change” occurs. Generally, an
ownership change occurs when certain shareholders increase their aggregate ownership by more than 50 percentage points

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

over their lowest ownership percentage in a testing period (typically three years). The Company has evaluated whether one
or more ownership changes under Section 382 have occurred since its inception and has determined that there have been at
least  two  such  changes.  Although  the  Company  believes  that  these  ownership  changes  have  not  resulted  in  material
limitations  on  its  ability  to  use  these  NOLs,  its  ability  to  utilize  these  NOLs  may  be  limited  due  to  future  ownership
changes or for other reasons. As a result, the Company may not be able to take full advantage of its carryforwards for U.S.
Federal, state, and foreign tax purposes.

Valuation Allowance

At December 31, 2020 and 2019, the Company maintained a full valuation allowance on its deferred tax assets since it
has  not  yet  achieved  sustained  profitable  operations.  As  a  result,  the  Company  has  not  recorded  any  income  tax  benefit
since its inception. In 2020, the valuation allowance for deferred tax assets increased by approximately $82.8 million. This
includes an increase of $26.3 million, $4.4 million and $43.4 million for U.S. Federal, state and foreign tax, respectively,
and  an  increase  of  $8.7  million  to  equity.  The  increase  in  equity  primarily  relates  to  the  foreign  currency  translation.  In
2019, the valuation allowance for deferred tax assets increased by approximately $14.8 million. This includes an increase
of $14.8 million, $2.6 million and $19.3 million for U.S. Federal, state and foreign tax, respectively, partially offset by a
decrease  of  $21.9  million  to  equity.  The  decrease  to  equity  primarily  related  to  the  U.S.  Federal  and  state  impact  of  the
equity component associated with the 2026 Convertible Notes.

Unrecognized Tax Benefits

At December 31, 2020 and 2019, the Company had no reserves for unrecognized tax benefits.

The Company and its subsidiaries are subject to taxation in the United States and various foreign jurisdictions. Of the
major jurisdictions, the Company is subject to U.S. Federal and state examinations for 2017 and forward, and 2016 and
forward, respectively, and examinations in the United Kingdom for 2017 and forward. However, NOLs are subject to audit
in any tax year in which those losses are utilized, notwithstanding the year of origin.

18. Net Loss Per Share

Basic loss per share is computed by dividing net loss attributable to common stockholders (numerator) by the weighted
average number of common shares outstanding (denominator) during the period. For the years ended December 31, 2020,
2019 and 2018, as the Company was in a net loss position, the diluted loss per share computations for such periods did not
assume the exercise of stock options or vesting of RSUs, or the conversion of Convertible Notes as they would have had an
anti-dilutive effect on loss per share.

The following potentially dilutive securities have been excluded from the computations of diluted weighted average

shares outstanding as of December 31, 2020, 2019 and 2018 as the inclusion thereof would have been anti-dilutive:

Shares issuable upon conversion of Convertible Notes
Options
Unvested restricted stock units
Total

2020

4,435
2,395  
902  
7,732  

December 31, 
2019
(in thousands)
4,435
1,981  
556  
6,972  

2018

2,316
1,874
441
4,631

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

19. Commitments and Contingencies

Facility Leases

In January 2016, Intercept Pharma Europe Ltd. (“IPEL”), a wholly owned subsidiary of the Company, entered into an
underlease  (sublease)  with  respect  to  office  space  in  London,  United  Kingdom.  The  Company  is  the  guarantor  to  the
underlease (sublease). IPEL leases approximately 8,600 square feet. The lease covering this property is scheduled to expire
in May 2024.

In November 2019, the Company entered into an amendment to the lease agreement with respect to office space at 10
Hudson Yards in New York, New York, where the Company’s corporate headquarters are located. The Company leases an
aggregate  of  approximately  45,600  square  feet  of  office  space  at  this  property.  The  lease  covering  this  property  is
scheduled to expire in March 2022.

In October 2019, the Company entered into a lease agreement with respect to office space in San Diego, California.
The Company leases approximately 34,000 square feet. The lease covering this property is scheduled to expire in October
2025.

The Company also leases office space in several other locations.

Licenses

The Company acquired a license from a third party to support the portfolio of product candidates. Under the license
agreement  with  Aralez  Pharmaceuticals  Canada  Inc.  (“Aralez”)  the  Company  has  rights  to  develop  and  commercialize
bezafibrate in the United States. The Company may pay up to $4.5 million upon the achievement of certain milestones,
none  of  which  is  owed  as  of  December  31,  2020.  The  Company  is  obligated  to  pay  royalties  to  at  a  mid-single  digit
percentage of net product sales.

Legal Proceedings

The Company is involved in various disputes, legal proceedings and litigation in the course of its business, including
the matters described below and, from time to time, governmental inquiries and investigations and employment and other
litigation. These matters, which could result in damages, fines or other administrative, civil or criminal remedies, liabilities
or penalties, are often complex and the outcome of such matters is often uncertain. The Company may from time to time
enter into settlements to resolve such matters.

Shareholder Litigation

On  September  27,  2017,  a  purported  shareholder  class  action,  initially  styled  DeSmet  v.  Intercept  Pharmaceuticals,
Inc., et al., was filed in the United States District Court for the Southern District of New York, naming the Company and
certain  of  its  officers  as  defendants.  The  Court  appointed  lead  plaintiffs  in  the  lawsuit  on  June  1,  2018,  and  the  lead
plaintiffs filed an amended complaint on July 31, 2018, captioned Hou Liu and Amy Fu v. Intercept Pharmaceuticals, Inc.,
et  al.,  naming  the  Company  and  certain  of  its  current  and  former  officers  as  defendants.  The  lead  plaintiffs  claim  to  be
suing on behalf of anyone who purchased or otherwise acquired the Company’s common stock between June 9, 2016 and
September 20, 2017. This lawsuit alleges that material misrepresentations and/or omissions of material fact were made in
the  Company’s  public  disclosures  during  the  period  from  June  9,  2016  to  September  20,  2017,  in  violation  of  Sections
10(b) and 20(a) of the Securities Exchange Act of 1934, as amended (the “Exchange Act”), and Rule 10b-5 promulgated
thereunder.  The  alleged  improper  disclosures  relate  to  statements  regarding  Ocaliva  dosing,  use  and  pharmacovigilance-
related matters, as well as the Company’s operations, financial performance and prospects. The plaintiffs seek unspecified
monetary damages on behalf of the putative class, an award of costs and expenses, including attorney’s fees, and rescissory

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

damages. On September 14, 2018, the Company filed a motion to dismiss the amended complaint. On March 26, 2020, the
Court granted the Company’s motion to dismiss the amended complaint in its entirety, and on March 27, 2020 the Court
entered judgment in favor of the Company. On May 8, 2020, the plaintiffs filed a motion to set aside the judgment and
grant leave to file a second amended complaint. On September 9, 2020, the Court denied the plaintiffs’ motion to set aside
the judgment and grant leave to file a second amended complaint, finding that the proposed second amended complaint did
not cure the deficiencies identified in the amended complaint. On October 9, 2020, the plaintiffs filed a notice of appeal to
the United States Court of Appeals for the Second Circuit and on January 25, 2021, the plaintiffs filed an appellate brief
challenging the March 27, 2020 judgment, the September 9, 2020 judgment and other orders entered in this action.

Separately, on December 1, 2017, a purported shareholder demand was made on the Company based on substantially
the same allegations as those set forth in the securities case above. In addition, on January 5, 2018, a follow-on derivative
suit, styled Davis v. Pruzanski, et al., was filed in New York state court by shareholder Gregg Davis based on substantially
the same allegations as those set forth in the securities case above.

On November 5, 2020, a purported shareholder class action, styled Chauhan v. Intercept Pharmaceuticals, Inc., et al.,
was filed in the United States District Court for the Eastern District of New York, naming the Company and certain of its
officers  as  defendants.  The  lawsuit  was  transferred  to  the  United  States  District  Court  for  the  Southern  District  of  New
York on January 4, 2021. The plaintiff claims to be suing on behalf of anyone who purchased or otherwise acquired the
Company’s  securities  between  September  28,  2019  and  October  7,  2020.  This  lawsuit  alleges  that  material
misrepresentations  and/or  omissions  of  material  fact  were  made  in  the  Company’s  public  disclosures  during  the  period
from September 28, 2019 to October 7, 2020, in violation of Sections 10(b) and 20(a) of the Exchange Act, and Rule 10b-5
promulgated  thereunder.  The  alleged  improper  disclosures  relate  to  statements  regarding  the  Company’s  New  Drug
Application for OCA for the treatment of liver fibrosis due to NASH and the use of Ocaliva in patients with PBC, as well
as the Company’s operations, financial performance and prospects. The plaintiff seeks unspecified monetary damages on
behalf of the putative class, and an award of costs and expenses, including attorney’s fees.

Separately, on December 29, 2020, a follow-on derivative suit, styled Rabinovich v. Fundarò, et al., was filed in the
United States District Court for the Southern District of New York by shareholder Delfin Rabinovich based on substantially
the same allegations as those set forth in the securities case immediately above. This lawsuit was subsequently transferred
to the United States District Court for the District of Delaware on January 28, 2021. On February 1, 2021, a second follow-
on derivative suit, styled Fung v. Fundarò, et al., was filed in the United States District Court for the District of Delaware
based on the substantially same allegations as those set forth in the securities case immediately above and the Rabinovich
derivative action.

While  the  Company  believes  that  it  has  a  number  of  valid  defenses  to  the  claims  described  above  and  intends  to
vigorously  defend  itself,  the  matters  are  in  the  early  stages  of  litigation  and  no  assessment  can  be  made  as  to  the  likely
outcome of the matters or whether they will be material to the Company. Accordingly, an estimate of the potential loss, or
range of loss, if any, to the Company relating to the matters is not possible at this time.

Patent Litigation

The  Company  has  received  paragraph  IV  certification  notice  letters  from  six  generic  drug  manufacturers  indicating
that each such manufacturer has submitted to the FDA an Abbreviated New Drug Application (“ANDA”) seeking approval
to  manufacture  and  sell  a  generic  version  of  the  Company’s  5  mg  and  10  mg  dosage  strengths  of  Ocaliva®  (obeticholic
acid) for PBC prior to the expiration of certain patents protecting Ocaliva.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Apotex Abbreviated New Drug Application

In July 2020, the Company received a paragraph IV certification notice (the “Apotex PIV Notice”) from Apotex Inc.
(“Apotex”) indicating that Apotex has submitted to the FDA an ANDA seeking approval to manufacture and sell a generic
version of the Company’s 5 mg and 10 mg dosage strengths of Ocaliva® (obeticholic acid) for PBC prior to the expiration
of the Company’s U.S. Patents Nos. 9,238,673 (the “‘673 Patent”), 10,047,117 (the “‘117 Patent”), 10,052,337 (the “‘337
Patent”),  and  10,174,073  (the  “‘073  Patent”,  and  collectively  with  the  ‘673  Patent,  ‘117  Patent  and  ‘337  Patent,  the
“Apotex  Challenged  Patents”),  which  are  listed  for  Ocaliva  in  the  FDA’s  Approved  Drug  Products  with  Therapeutic
Equivalence Evaluations (referred to as the “Orange Book”). The Apotex PIV Notice alleges that the Apotex Challenged
Patents are invalid, unenforceable, and/or will not be infringed by the commercial manufacture, use or sale of the generic
products  described  in  Apotex’s  ANDA.  Apotex  did  not  make  a  paragraph  IV  certification  against  the  Company’s  U.S.
Patents Nos. 7,138,390 (the “‘390 Patent”), 8,058,267 (the “‘267 Patent”) or 8,377,916 the (“‘916 Patent”), which are also
listed  for  Ocaliva  in  the  Orange  Book.  The  Company  initiated  a  patent  infringement  suit  against  Apotex  in  the  United
States District Court for the District of Delaware within 45 days of receipt of the Apotex PIV Notice. As a result, under the
Drug Price Competition and Patent Term Restoration Act of 1984 (the “Hatch-Waxman Act”), the FDA cannot grant final
approval  to  Apotex’s  ANDA  before  November  27,  2023  or  a  court  decision  in  Apotex’s  favor,  whichever  is  earlier.
Recently,  the  U.S.  Patent  and  Trademark  Office  (the  “USPTO”)  awarded  the  Company  two  additional  Orange  Book-
listable patents that protect Ocaliva: U.S. Patents Nos. 10,751,349 (the “‘349 Patent”) and 10,758,549 (the “‘549 Patent”).
In September and October 2020, the Company received additional amended paragraph IV certification notices from Apotex
challenging  the  ‘349  Patent  and  the  ‘549  Patent,  respectively.  The  Company  amended  its  complaint  against  Apotex  in
November  2020  to  add  infringement  allegations  for  the  ‘549  Patent.  In  January  2021,  the  Company  received  a  further
paragraph IV certification notice from Apotex challenging a reissue patent, U.S. Patent No. RE48,286 (the “‘286 Patent”),
as described below. The Company is evaluating its legal options, including asserting the ‘286 Patent against Apotex.

Lupin Abbreviated New Drug Application

In July 2020, the Company received a paragraph IV certification notice (the “Lupin PIV Notice”) from Lupin Limited
(“Lupin”) indicating that Lupin has submitted to the FDA an ANDA seeking approval to manufacture and sell a generic
version of the Company’s 5 mg and 10 mg dosage strengths of Ocaliva® (obeticholic acid) for PBC prior to the expiration
of  the  ‘390  Patent,  the  ‘673  Patent,  the  ‘117  Patent,  the  ‘337  Patent  and  the  ‘073  Patent  (collectively,  the  “Lupin
Challenged Patents”), which are listed for Ocaliva in the FDA’s Orange Book. The Lupin PIV Notice alleges that the Lupin
Challenged Patents are invalid, unenforceable, and/or will not be infringed by the commercial manufacture, use or sale of
the generic products described in Lupin’s ANDA. Lupin did not make a paragraph IV certification against the ‘267 Patent
or the ‘916 Patent, which are also listed for Ocaliva in the Orange Book. The Company initiated a patent infringement suit
against Lupin in the United States District Court for the District of Delaware within 45 days of receipt of the Lupin PIV
Notice.  As  a  result,  under  the  Hatch-Waxman  Act,  the  FDA  cannot  grant  final  approval  to  Lupin’s  ANDA  before
November 27, 2023 or a court decision in Lupin’s favor, whichever is earlier. In September 2020, the Company received an
additional  amended  paragraph  IV  certification  notice  from  Lupin  challenging  the  ‘349  Patent  and  the  ‘549  Patent.  The
Company amended its complaint against Lupin in November 2020 to add infringement allegations for the ‘549 Patent and
to substitute the ‘286 Patent for the ‘390 Patent.

Amneal Abbreviated New Drug Application

In  July  2020,  the  Company  received  a  paragraph  IV  certification  notice  (the  “Amneal  PIV  Notice”)  from  Amneal
Pharmaceuticals  of  New  York,  LLC,  as  U.S.  agent  for  Amneal  EU  Limited  (“Amneal”),  indicating  that  Amneal  has
submitted to the FDA an ANDA seeking approval to manufacture and sell a generic version of the Company’s 5 mg and 10
mg dosage strengths of Ocaliva® (obeticholic acid) for PBC prior to the expiration of the ‘673 Patent, the ‘117 Patent, the
‘337 Patent and the ‘073 Patent (collectively, the “Amneal Challenged Patents”), which are listed for Ocaliva in the FDA’s
Orange Book. The Amneal PIV Notice alleges that the Amneal Challenged Patents are invalid, unenforceable, and/or will
not be infringed by the commercial manufacture, use or sale of the generic products described in Amneal’s

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

ANDA.  Amneal  did  not  make  a  paragraph  IV  certification  against  the  ‘390  Patent,  the  ‘267  Patent  or  the  ‘916  Patent,
which are also listed for Ocaliva in the Orange Book. The Company initiated a patent infringement suit against Amneal in
the  United  States  District  Court  for  the  District  of  Delaware  within  45  days  of  receipt  of  the  Amneal  PIV  Notice.  As  a
result, under the Hatch-Waxman Act, the FDA cannot grant final approval to Amneal’s ANDA before November 27, 2023
or a court decision in Amneal’s favor, whichever is earlier. In October 2020, the Company received an additional amended
paragraph IV certification notice from Amneal challenging the ‘349 Patent and the ‘549 Patent. The Company amended its
complaint against Amneal in November 2020 to add infringement allegations for the ‘349 Patent and the ‘549 Patent.

Optimus Abbreviated New Drug Application

In  July  2020,  the  Company  received  a  paragraph  IV  certification  notice  (the  “Optimus  PIV  Notice”)  from  Optimus
Pharma Pvt Ltd (“Optimus”) indicating that Optimus has submitted to the FDA an ANDA seeking approval to manufacture
and sell a generic version of the Company’s 5 mg and 10 mg dosage strengths of Ocaliva® (obeticholic acid) for PBC prior
to the expiration of the ‘390 Patent, the ‘673 Patent, the ‘117 Patent, the ‘337 Patent and the ‘073 Patent (collectively, the
“Optimus Challenged Patents”) which are listed for Ocaliva in the FDA’s Orange Book. The Optimus PIV Notice alleges
that  the  Optimus  Challenged  Patents  are  invalid,  unenforceable,  and/or  will  not  be  infringed  by  the  commercial
manufacture,  use  or  sale  of  the  generic  products  described  in  Optimus’s  ANDA.  Optimus  did  not  make  a  paragraph  IV
certification against the ‘267 Patent or the ‘916 Patent, which are also listed for Ocaliva in the Orange Book. The Company
initiated a patent infringement suit against Optimus in the United States District Court for the District of Delaware within
45  days  of  receipt  of  the  Optimus  PIV  Notice.  As  a  result,  under  the  Hatch-Waxman  Act,  the  FDA  cannot  grant  final
approval to Optimus’s ANDA before November 27, 2023 or a court decision in Optimus’s favor, whichever is earlier. In
October 2020, the Company received an additional amended paragraph IV certification notice from Optimus challenging
the  ‘349  Patent  and  the  ‘549  Patent.  The  Company  amended  its  complaint  against  Optimus  in  November  2020  to  add
infringement allegations for the ‘549 Patent and to substitute the ‘286 Patent for the ‘390 Patent.

MSN Abbreviated New Drug Application

In  July  2020,  the  Company  received  a  paragraph  IV  certification  notice  (the  “MSN  PIV  Notice”)  from  MSN
Pharmaceuticals Inc. and MSN Laboratories Private Limited (collectively, “MSN”) indicating that MSN has submitted to
the FDA an ANDA seeking approval to manufacture and sell a generic version of the Company’s 5 mg and 10 mg dosage
strengths of Ocaliva® (obeticholic acid) for PBC prior to the expiration of the ‘390 Patent, the ‘673 Patent, the ‘117 Patent,
the ‘337 Patent and the ‘073 Patent (collectively, the “MSN Challenged Patents”) which are listed for Ocaliva in the FDA’s
Orange Book. The MSN PIV Notice alleges that the MSN Challenged Patents are invalid, unenforceable, and/or will not be
infringed by the commercial manufacture, use or sale of the generic products described in MSN’s ANDA. MSN did not
make a paragraph IV certification against the ‘267 Patent or the ‘916 Patent, which are also listed for Ocaliva in the Orange
Book. The Company initiated a patent infringement suit against MSN in the United States District Court for the District of
Delaware within 45 days of receipt of the MSN PIV Notice. As a result, under the Hatch-Waxman Act, the FDA cannot
grant final approval to MSN’s ANDA before November 27, 2023 or a court decision in MSN’s favor, whichever is earlier.
In November 2020, the Company received an additional paragraph IV certification notice from MSN challenging the ‘349
Patent, the ‘549 Patent, and the ‘286 Patent. The Company amended its complaint against MSN in November 2020 to add
infringement allegations for the ‘549 Patent and to substitute the ‘286 Patent for the ‘390 Patent.

DRL Abbreviated New Drug Application

In  December  2020,  the  Company  received  a  paragraph  IV  certification  notice  (the  “DRL  PIV  Notice”)  from  Dr.
Reddy’s Laboratories, Inc. and Dr. Reddy’s Laboratories, Ltd. (collectively, “DRL”) indicating that DRL has submitted to
the FDA an ANDA seeking approval to manufacture and sell a generic version of the Company’s 5 mg and 10 mg dosage
strengths of Ocaliva® (obeticholic acid) for PBC prior to the expiration of the ‘286 Patent, the ‘390 Patent, the ‘673 Patent,
the ‘117 Patent, the ‘337 Patent, the ‘073 Patent, the ‘349 Patent and the ‘549 Patent (collectively, the “DRL Challenged
Patents”) which are listed for Ocaliva in the FDA’s Orange Book. The DRL PIV Notice alleges that the DRL

F-40

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Challenged Patents are invalid, unenforceable, and/or will not be infringed by the commercial manufacture, use or sale of
the generic products described in DRL’s ANDA. DRL did not make a paragraph IV certification against the ‘267 Patent or
the ‘916 Patent, which are also listed for Ocaliva in the Orange Book. The Company initiated a patent infringement suit
against  DRL  in  the  United  States  District  Court  for  the District  of  Delaware  within  45  days  of  receipt  of  the  DRL  PIV
Notice. As a result, under the Hatch-Waxman Act, the FDA cannot grant final approval to DRL’s ANDA before November
27, 2023 or a court decision in DRL’s favor, whichever is earlier.

In  October  2020,  the  USPTO  granted  to  the  Company  a  reissue  patent,  ‘286  Patent.  By  operation  of  law,  the  ‘390
Patent was withdrawn and replaced by the ‘286 Patent, which contains composition of matter claims to OCA and has the
same term as the ‘390 Patent. In November 2020, the Company was informed by the USPTO that its petition for a five-year
patent  term  extension  of  the  ‘286  Patent  had  been  granted  and  that  the  ‘286  Patent  will  now  expire  in  2027.  The  ‘286
Patent has been listed in the Orange Book.

These proceedings are costly and time consuming. Successful challenges to the Company’s patent or other intellectual
property rights through these proceedings could result in a loss of rights in the relevant jurisdiction and may allow third
parties to use the Company’s proprietary technologies without a license from the Company or its collaborators. While the
Company  intends  to  vigorously  defend  and  enforce  its  intellectual  property  rights  protecting  Ocaliva,  the  Company  can
offer  no  assurance  as  to  when  the  lawsuits  will  be  decided,  whether  the  lawsuits  will  be  successful,  or  that  a  generic
equivalent of Ocaliva will not be approved and enter the market before the expiration of the Company’s patents.

20. Quarterly Financial Data (unaudited)

The  following  table  summarizes  the  unaudited  quarterly  financial  data  for  the  years  ended  December  31,  2020  and

2019:

     March 31,       June 30, 

    September 30,     December 31,     

Total

(in thousands, except for per share amounts)

Quarters Ended

2020

Total revenue
Operating loss
Net loss
Net loss per common share - basic and diluted (1)

2019

Total revenue
Operating loss
Net loss
Net loss per common share - basic and diluted (1)

$ 72,652
  (83,445)
  (92,983)
$

$ 52,252
  (83,945)
  (90,270)
$

$

$ 77,249
  (52,030)
  (63,281)

$

79,521
(55,163)
(66,469)

(2.86) $

(1.92) $

(2.01) $

$

$ 66,300
  (63,659)
  (71,420)

$

61,950
(75,533)
(84,833)

(3.03) $

(2.28) $

(2.59) $

83,268
(40,602)
(52,147)
(1.58)

71,500
(89,290)
(98,158)
(2.99)

$ 312,690
(231,240)
(274,880)

$ 252,002
(312,427)
(344,681)

(1) Basic  and  diluted  net  loss  per  common  share  is  computed  independently  for  each  of  the  quarters  presented.
Therefore,  the  sum  of  quarterly  basic  and  diluted  net  loss  per  common  share  may  not  equal  annual  basic  and
diluted net loss per common share.

F-41

 
 
 
 
 
 
 
  
 
   
   
   
   
  
 
 
 
 
 
 
 
  
              
Description of the Registrant's Securities Registered Pursuant to Section 12 of the Securities Exchange Act of
1934

Description of the Registrant's Common Stock

References  to  “Intercept,"  "our"  and  the  “Company”  herein  are,  unless  the  context  otherwise  indicates,  only  to
Intercept Pharmaceuticals, Inc. and not to any of its subsidiaries.

Exhibit 4.11

Description of Common Stock

General

The  following  is  a  summary  of  information  concerning  Intercept's  common  stock,  par  value  $0.001  per  share
("Common Stock"). The summaries and descriptions below do not purport to be complete statements of the relevant
provisions of our restated certificate of incorporation and restated bylaws and are entirely qualified by, and should be
read in conjunction with, these documents, each of which is filed as an exhibit to the Annual Report on Form 10-K of
which this Exhibit 4.11 is a part.

Common Stock

Authorized  Capital  Stock  and  Shares  Outstanding.  Our  authorized  capital  stock  consists  of  90,000,000  shares  of
Common  Stock  and  5,000,000  shares  of  preferred  stock,  par  value  $0.001  per  share.  As  of  December  31,  2020,
33,015,614 shares of Common Stock were outstanding, and no shares of preferred stock were outstanding. All of the
outstanding shares of our Common Stock are fully paid and nonassessable.

Annual Meeting. Annual meetings of our stockholders are held on the date designated in accordance with our restated
bylaws.  Written  notice  must  be  mailed  to  each  stockholder  entitled  to  vote  not  less  than  ten  nor  more  than  60  days
before the date of the meeting. The presence in person or by proxy of the holders of record of a majority of our issued
and outstanding shares entitled to vote at such meeting constitutes a quorum for the transaction of business at meetings
of the stockholders. Special meetings of the stockholders may be called for any purpose only by our board of directors
pursuant to a resolution adopted by a majority of the total number of directors. Except as may be otherwise provided
by applicable law, our restated certificate of incorporation or our restated bylaws, all elections shall be decided by a
plurality,  and  all  other  questions  shall  be  decided  by  a  majority,  of  the  votes  cast  by  stockholders  entitled  to  vote
thereon at a duly held meeting of stockholders at which a quorum is present.

Voting Rights.  Holders  of  our  Common  Stock  are  entitled  to  one  vote  for  each  share  held  of  record  on  all  matters
submitted to a vote of the stockholders and do not have cumulative voting rights.

Dividends.  Subject  to  preferences  that  may  be  applicable  to  any  outstanding  shares  of  preferred  stock,  holders  of
Common  Stock  are  entitled  to  receive  ratably  such  dividends,  if  any,  as  may  be  declared  from  time  to  time  by  our
board of directors out of funds legally available for dividend payments.

Liquidation  and  Dissolution.  In  the  event  of  any  liquidation,  dissolution  or  winding-up  of  our  affairs,  holders  of
Common Stock will be entitled to share ratably in any of our assets remaining after payment or provision for payment
of all of our debts and obligations and after liquidation payments to holders of outstanding shares of preferred stock, if
any.

Other Rights.  The  holders  of  Common  Stock  have  no  preferences  or  rights  of  conversion,  exchange,  preemptive  or
other subscription rights. There are no redemption or sinking fund provisions applicable to the Common Stock.

Transfer Agent and Registrar. VStock Transfer, LLC is transfer agent and registrar for the Common Stock.

NASDAQ Global Select Market. Our Common Stock is listed on The Nasdaq Global Select Market under the symbol
“ICPT.”

Anti-takeover Effects of Our Restated Certificate of Incorporation, Restated Bylaws and Delaware Law

The provisions of Delaware law and our restated certificate of incorporation and restated bylaws could discourage or
make it more difficult to accomplish a proxy contest or other change in our management or the acquisition of control
by a holder of a substantial amount of our voting stock. It is possible that these provisions could make it more difficult
to accomplish, or could deter, transactions that stockholders may otherwise consider to be in their best interests or in
our best interests.

These provisions are intended to enhance the likelihood of continuity and stability in the composition of our board of
directors and in the policies formulated by the board of directors and to discourage certain types of transactions that
may involve an actual or threatened change of our control. These provisions are designed to reduce our vulnerability to
an unsolicited acquisition proposal and to discourage certain tactics that may be used in proxy fights. Such provisions
also may have the effect of preventing changes in our management.

Delaware Business Combination Statute. We are subject to the anti-takeover provisions of Section 203 of the Delaware
General Corporation Law, which we refer to as the DGCL. With some exception, Section 203 of the DGCL prohibits a
publicly-held Delaware corporation from engaging in a “business combination” with an “interested stockholder” for a
period of three years after the date of the transaction in which the person became an interested stockholder, unless the
business combination is, or the transaction in which the person became an interested stockholder was, approved by the
board of directors and the holders of at least two-thirds of the outstanding voting stock of the corporation. The shares
held by the interested stockholder are not counted as outstanding when calculating the two-thirds of the outstanding
voting  stock  needed  for  approval.  For  purposes  of  Section  203  of  the  DGCL,  a  “business  combination”  is  defined
broadly to include a merger, asset sale or other transaction resulting in a financial benefit to the interested stockholder,
and, subject to certain exceptions, an “interested stockholder” is a person who, together with his or her affiliates and
associates, owns, or within three years prior, did own, 15% or more of the corporation’s outstanding voting stock.

Advance Notice Provisions for Stockholder Proposals and Stockholder Nominations of Directors. Our restated bylaws
provide that, for nominations to the board of directors or for other business to be properly brought by a stockholder
before a meeting of stockholders, a stockholder must first have given timely notice of the proposal in writing to our
secretary. For an annual meeting, a stockholder’s notice generally must be delivered not less than 90 days nor more
than 120 days prior to the first anniversary of the previous year’s annual meeting date; provided, that if the date of the
annual meeting is more than 30 days before or more than 30 days after the anniversary of the previous year’s annual
meeting date, such stockholder’s notice must be delivered not earlier than the close of business on the 120 day prior to
such annual meeting and not later than the close of business on the later of the 90 day prior to such annual meeting or
the close of business on the 10 day following the day on which public announcement of the date of such meeting is
first made by us. For a special meeting, the notice must generally be delivered not earlier than the 90 day prior to the
meeting and not later than the later of (1) the 60 day prior to the meeting or (2) the 10 day following the day on which
public announcement of the meeting is first made. Detailed requirements as to the form of the notice and information
required in the notice are specified in the restated bylaws. If it is determined that business was not properly brought
before a meeting in accordance with our bylaws provisions, such business will not be conducted at the meeting.

Special Meetings of Stockholders. Special meetings of the stockholders may be called only by our board of directors
pursuant to a resolution adopted by a majority of the total number of directors.

No Stockholder Action by Written Consent. Any action to be effected by our stockholders must be effected at a duly
called  annual  or  special  meeting  of  the  stockholders  provided,  however,  our  restated  certificate  of  incorporation
provides that if any one stockholder, together with its affiliates, collectively holds a majority of the voting power of

the then-outstanding shares of our capital stock, action may be taken without a meeting and vote, through the written
consent of holders of the requisite number of votes necessary to authorize or take such action at a meeting.

Board  of  Directors.  We  do  not  have  a  classified  board  of  directors.  All  of  our  directors  are  elected  annually.  The
number of directors comprising our board of directors is fixed from time to time by the board of directors.

Removal of Directors by Stockholders. Our restated bylaws provide that our directors may be removed with or without
cause by the affirmative vote of the holders of a majority of the votes that all our stockholders would be entitled to cast
in  an  annual  election  of  directors,  and  our  restated  certificate  of  incorporation  and  restated  bylaws  provide  that  any
vacancy on our board of directors, including a vacancy resulting from an increase in the size of our board of directors,
may be filled only by vote of a majority of our directors then in office.

Super Majority Stockholder Vote Required for Certain Actions. The DGCL provides generally that the affirmative vote
of  a  majority  of  the  shares  entitled  to  vote  on  any  matter  is  required  to  amend  a  corporation’s  certificate  of
incorporation or bylaws, unless the corporation’s certificate of incorporation or bylaws, as the case may be, requires a
greater percentage. Our restated certificate of incorporation requires the affirmative vote of the holders of at least 80%
of  our  outstanding  voting  stock  to  amend  or  repeal  any  of  the  provisions  discussed  in  this  section  of  this  Exhibit
entitled  “Anti-takeover  Effects  of  Our  Restated  Certificate  of  Incorporation,  Restated  Bylaws  and  Delaware  Law.”
This 80% stockholder vote would be in addition to any separate class vote that might in the future be required pursuant
to  the  terms  of  any  preferred  stock  that  might  then  be  outstanding.  The  affirmative  vote  of  at  least  80%  of  our
outstanding voting stock is also required for any amendment to, or repeal of, our restated bylaws by the stockholders.
Our restated bylaws may be amended or repealed by a simple majority vote of the board of directors.

Exhibit 10.21

EMPLOYMENT AGREEMENT

THIS  EMPLOYMENT  AGREEMENT  (the  “Agreement”),  made  effective  as  of  December  18th,  2020,  is

entered into by Intercept Pharmaceuticals, Inc. (the “Company”) and Jared Freedberg (“Executive”).

WHEREAS,  the  Company  desires  to  employ  Executive,  and  Executive  desires  to  be  employed  by  the

Company.

NOW  THEREFORE,  in  consideration  of  the  mutual  covenants  and  promises  contained  in  this  Agreement,
and  other  good  and  valuable  consideration,  the  receipt  and  sufficiency  of  which  are  hereby  acknowledged  by  the
parties to this Agreement, the parties agree as follows:

1. Term of Employment.  The Company hereby agrees to employ Executive, and Executive hereby accepts
employment with the Company, upon the terms set forth in this Agreement, for the period commencing on February
1st, 2021 or such date as may be otherwise agreed upon with the Company (the “Commencement Date”) and ending
on  the  one  year  anniversary  thereof,  unless  sooner  terminated  in  accordance  with  the  provisions  of  Section  4  (such
period,  the  “Initial  Term”);  provided,  however,  that  on  each  anniversary  of  the  Commencement  Date,  the  term  of
employment  under  this  Agreement  shall  be  automatically  extended  for  an  additional  one-year  period  (each  such
period, a “Subsequent Term”) unless terminated sooner pursuant to Section 4 or if, at least thirty (30) days prior to the
applicable anniversary date, either Executive or the Company provides written notice to the other party electing not to
extend.  The Initial Term together with each Subsequent Term, if any, are referred to hereinafter as the “Agreement
Term.”

2. Title;  Capacity.    During  the  Agreement  Term,  the  Company  will  employ  Executive  as  its  General
Counsel  &  Company  Secretary  to  perform  the  duties  and  responsibilities  inherent  in  such  position  and  such  other
duties and responsibilities consistent with such position as the President & Chief Executive Officer of the Company
(the “CEO”) shall from time to time reasonably assign to him.  On an annual basis, the Company’s Board of Directors
(the “Board”) in consultation with Executive and the CEO, will set reasonably attainable, specific goals pursuant to the
objectives  of  the  Company  as  in  effect  from  time  to  time.    Executive  shall  report  directly  to  the  CEO  and  shall  be
subject to the supervision of, and shall have such authority as is delegated to Executive by, the CEO, which authority
shall be sufficient to perform Executive’s duties hereunder. Executive will be based at the Company’s headquarters in
New  York,  New  York.    Subject  to  Section  4.3  below,  the  location  of  Executive’s  employment  is  subject  to  change
during the course of the Agreement Term as determined by the CEO in consultation with the Executive.  Executive
hereby accepts such employment and agrees to undertake the duties and responsibilities inherent in such position and
such other duties as may be reasonably assigned to Executive. Executive shall devote substantially all of his business
time,  energies  and  attention  in  the  performance  of  the  foregoing  services.    Notwithstanding  the  foregoing,  nothing
herein shall preclude Executive from (i) performing services for such other companies as the Company may designate
or permit, (ii) serving, with the prior written consent of the Board, which consent shall not be unreasonably withheld,
as  an  officer  or  member  of  the  boards  of  directors  or  advisory  boards  (or  their  equivalents  in  the  case  of  a  non-
corporate  entity)  of  non-competing  businesses,  (iii)  serving  as  an  officer  or  a  member  of  charitable,  educational  or
civic  organizations,  (iv)  engaging  in  charitable  activities  and  community  affairs,  and  (v)  managing  Executive’s
personal investments and affairs; provided, however, that the activities set out in clauses (i) – (v) shall be limited by
Executive so as not to materially interfere, individually or in the aggregate, with the performance of Executive’s duties
and responsibilities hereunder.

3. Compensation and Benefits.

3.1

 Salary.  The Company shall pay Executive an initial annualized base salary of $461,600.00,
payable  in  accordance  with  the  Company’s  regular  payroll  practices.    Such  base  salary  shall  be  subject  to  annual
review  and  increase  (but  not  decrease)  as  may  be  determined  and  approved  by  the  Board  or  the  Company’s
Compensation Committee in its sole discretion.  

3.2

Bonuses.  

Exhibit 10.21

(a)

Annual  Bonus.  At  the  end  of  a  given  fiscal  year,  Executive  will  be  eligible  to
receive a bonus based on a target equal to 50% of his base salary in effect at the end of such fiscal year. Executive’s
annual  bonus  for  the  fiscal  year  in  which  the  Commencement  Date  occurs  shall  be  based  upon  his  annualized  base
salary and shall not be prorated. The amount of any such bonus shall be based on factors including, but not limited to,
Executive’s  achievement,  as  determined  by  the  Board  or  the  Compensation  Committee  of  the  Board  (the
“Compensation Committee”) in its sole discretion, of reasonable goals and milestones established in advance by the
Board or the Compensation Committee in consultation with the CEO and Executive.  The period for calculation of the
bonus shall be consistent with the Company’s fiscal year.  Such bonus, if any, will be paid to Executive on or after
January 1 and in any case no later than March 15 of the immediately succeeding fiscal year.  The bonus shall be paid in
cash; provided that, if requested by Executive and approved by the Board, some or all of the bonus may be paid in
equity under the Company’s stockholder approved stock plan then in effect (valued at the fair market value thereof), or
any combination of the foregoing.  To the extent that the Company is required pursuant to Section 954 of the Dodd-
Frank Wall Street Reform and Consumer Protection Act to develop and implement a policy (the “Policy”) providing
for the recovery from the Executive of any payment of incentive-based compensation paid to the Executive that was
based  upon  erroneous  data  contained  in  an  accounting  statement,  this  Agreement  shall  be  deemed  amended  and  the
Policy incorporated herein by reference as of the date that the Company takes all necessary corporate action to adopt
the Policy, without requiring any further action of the Company or the Executive, provided that any such Policy shall
only be binding on the Executive if the same Policy applies to the Company’s other executive officers.

3.3

Equity Awards.  

(a)

On the Commencement Date, the Company shall grant Executive (i) a stock option
under its 2012 Equity Incentive Plan (as amended from time to time, the “2012 Plan”) to purchase 69,400 shares of the
Company’s common stock at a per share exercise price equal to the closing price of the common stock on the date of
grant (the “Time-Based Option”), and (ii) a restricted stock award for 44,277 shares of the Company’s common stock
(the “Restricted Stock”).

(b)

Each  of  the  Time-Based  Option  and  the  Restricted  Stock  will  be  evidenced  in
writing by an agreement provided by the Company. The Time-Based Option shall vest as follows: (i) one-quarter of
the Time-Based Option will vest on the first anniversary of the Commencement Date; and (ii) the remaining balance
will vest in equal monthly installments in arrears over the three (3) year period commencing on the first anniversary of
the Commencement Date and ending on the fourth anniversary of the Commencement Date, all subject to Executive’s
continued  employment  by  the  Company  and  the  terms  of  the  2012  Plan,  except  as  otherwise  set  forth  herein.  The
Time-Based Option agreement will specify that vested options shall be exercisable for up to ten (10) years, subject to
the terms of this Agreement and the 2012 Plan. The shares underlying the Restricted Stock shall vest as follows: (x)
one-quarter of the shares underlying the Restricted Stock will vest on the first anniversary of the Commencement Date;
and  (y)  the  remaining  balance  will  vest  in  equal  quarterly  installments  in  arrears  over  the  three  (3)  year  period
commencing  on  the  first  anniversary  of  the  Commencement  Date  and  ending  on  the  fourth  anniversary  of  the
Commencement  Date,  all  subject  to  Executive’s  continued  employment  by  the  Company  and  the  terms  of  the  2012
Plan, except as otherwise set forth herein.

additional stock options or other equity-based awards may be granted to Executive from time to time.  

(c)

At  the  sole  discretion  of  the  Board  or  the  Company’s  Compensation  Committee,

3.4

Fringe Benefits.  Executive shall be entitled to participate in all bonus and benefit programs
that the Company establishes and makes available to its U.S.-based executives and/or employees from time to time,
including, but not limited to, health care plans, dental care plans, vision care plans, supplemental retirement plans, life
insurance plans, disability insurance plans and incentive compensation plans, to the extent that Executive is eligible
under,  and  subject  to  the  terms  and  conditions  of,  the  applicable  plan  documents  governing  such  programs.    The
Company shall pay 100% of the premium cost for health insurance coverage for Executive, his spouse and children,
provided  that  his  spouse  and  dependents  are  not  covered  by  an  equivalent  health  insurance  plan  provided  by  his
spouse’s employer.  Executive shall be eligible to accrue up to four (4) weeks of paid vacation each calendar year (to
be taken at such times and in such number of days as Executive shall determine in consultation with the CEO and in a
manner  so  as  not  to  impair  or  otherwise  interfere  with  Executive’s  ability  to  perform  his  duties  and  responsibilities
hereunder).    The  vacation  days  for  which  Executive  is  eligible  shall  accrue  at  the  rate  of  1.67  days  per  month  that
Executive is employed during such calendar year.  Vacation accrual will be capped at 1.75 times Executive’s annual

Exhibit 10.21

vacation accrual.  When Executive’s accrued vacation reaches the cap, he will not accrue additional vacation time until
some of the previously accrued vacation is used and the accrued amount falls below the cap, unless the Company is
acquired by another business venture, in which case none of the previous year’s accrued vacation will be subject to a
cap.  Executive shall also be eligible for paid holidays and paid sick days annually, in accordance with the Company’s
policies for its senior executives as in effect from time to time.  At the end of each calendar year, all unused sick days shall
be forfeited.

3.5

Reimbursement  of  Expenses.    The  Company  shall  reimburse  Executive  for  reasonable
travel,  entertainment  and  other  expenses  incurred  or  paid  in  connection  with,  or  related  to  the  performance  of
Executive’s  duties,  responsibilities  or  services  under  this  Agreement,  upon  presentation  by  Executive  of
documentation, expense statements, vouchers and/or such other supporting information as the Company may request.
Executive  must  submit  proper  documentation  for  each  such  expense  within  sixty  (60)  days  after  the  later  of  (i)  his
incurrence of such expense or (ii) his receipt of the invoice for such expense.  The Company will reimburse Executive
for that expense within thirty (30) days after receipt of the documentation.  

state and local taxes and withholdings, if any.

3.6

Withholdings.  Payments made under this Section 3 shall be subject to applicable federal,

4. Termination of Employment Period.  The Agreement Term shall terminate upon the occurrence of any of

the following:

Agreement Term; provided, that notice is given in accordance with Section 1 of this Agreement.

4.1

Expiration  of  the  Agreement  Term.    This  Agreement  shall  expire  at  the  end  of  the

4.2

Termination  by  the  Company  for  Cause.      At  the  election  of  the  Company,  the  Executive
may  be  terminated  by  the  Company  for  Cause  (as  defined  below),  immediately  following  written  notice  by  the
Company  to  Executive,  which  notice  shall  identify  in  reasonable  detail  the  Cause  upon  which  termination  is  based,
except that for reason 4.2(a)(iv) below, termination may not occur prior to the expiration of the thirty (30) day period
to cure.  For the purposes of this Agreement, “Cause” for termination shall be deemed to exist upon:  

(a)

a  good  faith  finding  by  the  Company  that  (i)  Executive  has  engaged  in  material
dishonesty, willful misconduct or gross negligence in connection with the performance of his duties; (ii) Executive has
committed any act of fraud or embezzlement with respect to the Company or any of its affiliates; (iii) Executive has
breached  or  has  threatened  to  breach  his  Invention,  Non-Disclosure,  and  Non-Solicitation  Agreement;  or  (iv)
Executive  has  materially  breached  this  Agreement,  and  Executive  has  failed  to  cure  such  conduct  or  breach  within
thirty (30) days after his receipt of written notice from the Company of such breach; or

involving moral turpitude, fraud or embezzlement, or any felony.

(b)

Executive’s  conviction,  guilty  plea,  or  entry  of  nolo  contendere  to  any  crime

4.3

Termination  By  Executive  with  Good  Reason.    Executive  may  terminate  the  Agreement
Term with Good Reason.  For purposes of this Agreement, “Good Reason” means the occurrence, without Executive’s
written  consent,  of  any  of  the  events  or  circumstances  set  forth  in  clauses  (a)  through  (c)  below.    In  addition,
notwithstanding the occurrence of any of the events enumerated in clauses (a) through (c), such occurrence shall not be
deemed  to  constitute  Good  Reason  if,  within  thirty  (30)  days  after  the  Company’s  receipt  of  written  notice  from
Executive of the occurrence or existence of an event or circumstance enumerated in clauses (a) through (c), such event
or  circumstance  has  been  remedied  by  the  Company.  Executive  shall  not  be  deemed  to  have  terminated  his
employment  with  Good  Reason  unless  Executive  first  delivers  a  written  notice  of  termination  to  the  Company
identifying  in  reasonable  detail  the  acts  or  omissions  constituting  Good  Reason  within  ninety  (90)  days  after  their
occurrence  and  the  provision  of  this  Agreement  relied  upon,  such  acts  or  omissions  are  not  cured  by  the  Company
within thirty (30) days of the receipt of such notice, and Executive actually ends his employment within one-hundred
and twenty (120) days after the Company’s failure to cure.

Executive’s position as General Counsel & Company Secretary (including status, offices, titles, authority, or

(a)

the  assignment  to  Executive  of  duties  inconsistent  in  any  material  respect  with

Exhibit 10.21

responsibilities) or any other action or omission by the Company which results in a material diminution in Executive’s
position, status, offices, titles, authority, responsibilities, or reporting requirements;

a  change  by  the  Company  in  the  location  at  which  Executive  performs  his
principal duties for the Company to a different location that is outside a radius of fifty (50) miles from (i) Executive’s
principal residence immediately prior to the date on which such change occurs and (ii) the location at which Executive
performed his principal duties for the Company immediately prior to the date on which such change occurs; or

(b)

agreement between the Company and Executive.

(c)

any  material  breach  by  the  Company  of  this  Agreement  or  any  other  material

4.4

Death or Disability.  This Agreement shall terminate upon Executive’s death or disability.
 As used in this Agreement, the determination of “disability” shall occur when Executive, due to a physical or mental
disability, for a period of 60 consecutive days, or 120 days in the aggregate whether or not consecutive, during any
360-day period, is unable to perform the services contemplated under this Agreement.  A determination of disability
shall  be  made  by  a  physician  satisfactory  to  both  Executive  and  the  Company;  provided, that,  if  Executive  and  the
Company do not agree on a physician, Executive and the Company shall each select a physician and these two together
shall select a third physician, whose determination as to disability shall be binding on all parties.  

Termination by Executive Without Good Reason or Termination by the Company Without
Cause.  At the election of Executive without Good Reason or by the Company without Cause, upon not less than thirty
(30) days’ prior written notice to the other party.

4.5

5. Effect of Termination.

5.1

Payments  Upon  Termination  for  Any  Reason.    In  the  event  Executive’s  employment
terminates pursuant to Section 4, the Company shall pay to Executive (or Executive’s estate or legal representative, if
applicable),  on  the  date  of  Executive’s  termination  of  employment  with  the  Company  (or  as  soon  thereafter  as  is
practicable,  consistent  with  applicable  law  and  the  terms  of  any  deferred  compensation  plan  or  agreement),  the
compensation and benefits under Sections 3.1, 3.4 and 3.5 that are accrued and unpaid through such termination date
(including, without limitation, an amount equal to all accrued but unused vacation pay and unreimbursed expenses).  In
the event of termination of Executive’s employment by Executive by reason of non-renewal of the Agreement Term
pursuant  to  Sections  1  and  4.1,  the  Company  for  Cause  pursuant  to  Section  4.2,  by  reason  of  Executive’s  death  or
disability pursuant to Section 4.4, or by Executive without Good Reason pursuant to Section 4.5, Executive shall not
receive any compensation or benefits other than as expressly stated in this Section 5.1 and as otherwise required by
law.

5.2

Termination by the Company Without Cause, by the Company by Reason of Non-Renewal
of Agreement Term, or by Executive for Good Reason.  Subject to Section 5.3 below, in addition to the payments and
provisions  under  Section  5.1,  in  the  event  of  termination  of  Executive’s  employment  by  the  Company  by  reason  of
non-renewal of the Agreement Term pursuant to Sections 1 and 4.1, by Executive for Good Reason pursuant to Section
4.3, or by the Company without Cause pursuant to Section 4.5, provided that Executive executes a release of claims
substantially in the form attached hereto as Exhibit A (the “Release”), which Release must be effective and irrevocable
prior  to  the  sixtieth  (60th)  day  following  the  termination  of  the  Executive’s  employment  (the  “Review  Period”),  the
Company shall provide Executive with the following:

 twelve (12) months of Executive’s base salary in effect at the time of termination
of employment, payable according to the Company’s payroll commencing on the first payroll date following the date
the Release is effective and irrevocable (the “Payment Date”), subject to compliance with Sections 5.5 and 12.6; and

(a)

(b)

the  Company  will,  for  a  period  of  twelve  (12)  months  following  Executive’s
termination from employment, continue Executive’s participation in the Company’s group health plan and dental plan
and shall pay that portion of the premiums that the Company paid on behalf of Executive and his dependents during
Executive’s employment, provided, however, that if the Company’s health insurance plan and/or dental plan does not
permit such continued participation in such plan after Executive’s termination of employment, then the Company shall

Exhibit 10.21

pay that portion of the premiums associated with COBRA continuation coverage that the Company paid on behalf of
Executive and his dependents during Executive’s employment, including any administrative fee, on Executive’s behalf
for  such  twelve-month  period;  and  provided,  further,  that  if  Executive  becomes  employed  with  another  employer
during  the  period  in  which  continued  health  insurance  and/or  dental  insurance  is  being  provided  pursuant  to  this
Section,  the  Company  shall  not  be  required  to  continue  such  health  and  dental  benefits,  or  if  applicable,  to  pay  the
costs of COBRA, if Executive becomes covered under a health insurance plan of the new employer.  (For purposes of
this  Section  5.2(b),  the  term  “Executive”  shall  include,  to  the  extent  applicable,  Executive’s  spouse  and  any  of
Executive’s dependents covered under the Company’s group health plan and/or dental plan prior to his termination of
employment.)

5.3

Termination in the Event of a Change in Control.

(a)

In addition to the payments and provisions under Section 5.1 but in lieu of, and not
in  addition  to,  the  payments  required  pursuant  to  Section  5.2  above,  in  the  event  Executive’s  employment  with  the
Company is terminated by the Company by reason of non-renewal of the Agreement Term pursuant to Sections 1 and
4.1, by Executive for Good Reason pursuant to Section 4.3, or by the Company without Cause pursuant to Section 4.5,
in  any  such  case  within  twelve  (12)  months  following  a  Change  in  Control  (as  defined  below)  provided  that  such
Change  in  Control  also  qualifies  as  a  “change  in  control  event”  within  the  meaning  of  Treasury  Regulation  Section
1.409A-3(i)(5)(i)  (where  required  to  avoid  the  imposition  of  penalty  taxes  under  Section  409A)  and  provided  that
Executive (or Executive’s legal representative, if applicable) executes a Release and the Release becomes effective and
irrevocable prior to the end of the Review Period, Executive shall be entitled to the following:

a lump sum cash amount equal to twelve (12) months of Executive’s base
salary  in  effect  at  the  time  of  Executive’s  termination,  such  payment  to  be  made  on  the  Payment  Date,  subject  to
compliance with Sections 5.5 and 12.6;

(i)

(ii)

for  up  to  twelve  (12)  months  after  Executive’s  date  of  termination,  the
Company shall continue Executive’s participation in the Company’s group health and dental plan and shall pay that
portion  of  the  premiums  that  the  Company  paid  on  behalf  of  Executive  and  his  dependents  during  Executive’s
employment; provided, however,  that  if  the  Company’s  health  insurance  plan  and/or  dental  insurance  plan  does  not
permit Executive’s continued participation in such plan after his termination of employment, then the Company shall
pay that portion of the premiums associated with COBRA continuation coverage that the Company paid on behalf of
Executive and his dependents during Executive’s employment, including administrative fees, on Executive’s behalf for
so  long  as  COBRA  continuation  coverage  is  available,  up  to  twelve  (12)  months;  and  provided,  further,  that  if
Executive  becomes  employed  with  another  employer  during  the  period  in  which  continued  health  insurance  and/or
dental insurance is being provided pursuant to this Section, the Company shall not be required to continue the relevant
benefits, or if applicable, to pay the relevant costs of COBRA, if Executive becomes covered under a health insurance
plan  and/or  dental  plan  of  the  new  employer.  (For  purposes  of  this  Section  5.3(a)(ii),  the  term  “Executive”  shall
include, to the extent applicable, Executive’s spouse and any of Executive’s dependents covered under the Company’s
group health plan and/or dental plan prior to his termination of employment.)

the following events occur:  

(b)

As used herein, “Change in Control” shall occur or be deemed to occur if any of

(i)
of transactions) of all or substantially all of the assets of the Company; or

any sale, lease, exchange or other transfer (in one transaction or a series

(ii)

any  consolidation  or  merger  of  the  Company  (including,  without
limitation,  a  triangular  merger)  where  the  shareholders  of  the  Company  immediately  prior  to  the  consolidation  or
merger,  would  not,  immediately  after  the  consolidation  or  merger,  beneficially  own,  directly  or  indirectly,  shares
representing  in  the  aggregate  more  than  fifty  percent  (50%)  of  the  combined  voting  power  of  all  the  outstanding
securities  of  the  corporation  issuing  cash  or  securities  in  the  consolidation  or  merger  (or  of  its  ultimate  parent
corporation, if any); or

Securities Exchange Act of 1934, as amended (the “Exchange Act”) (but other than (x) the Company, (y) any

(iii)

a third person, including a “person” as defined in Section 13(d)(3) of the

Exhibit 10.21

employee  benefit  plan  of  the  Company,  or  (z)  investors  purchasing  equity  securities  of  the  Company  pursuant  to  a
financing or a series of financings approved by the Board of Directors of the Company) becomes the beneficial owner
(as defined in Rule 13d-3 under the Exchange Act) directly or indirectly, of Controlling Securities (as defined below).
“Controlling Securities” shall mean securities representing 25% or more of the total number of votes that may be cast
for the election of the directors of the Company.

5.4

Effect of Termination on Stock Options and Other Equity Compensation.  

(a)

In the event of Executive’s termination by Executive by reason of non-renewal of
the  Agreement  Term  pursuant  to  Sections  1  and  4.1,  by  the  Company  for  Cause  pursuant  to  Section  4.2,  or  by
Executive  without  Good  Reason  pursuant  to  Section  4.5,  all  unvested  stock  options  and  other  equity-based  awards
granted to Executive before and after the date of this Agreement shall be immediately forfeited upon the effective date
of such termination of employment or as otherwise provided in the award agreement; provided, that, Executive shall
have until the earlier of the expiration date of the option or ninety (90) days from the date of termination of Executive
to exercise all vested options unless the stock plan pursuant to which the option is granted requires earlier termination
in connection with a liquidation or sale of the Company.

(b)

In the event of Executive’s termination by the Company by reason of non-renewal
of the Agreement Term pursuant to Sections 1 and 4.1, by Executive for Good Reason pursuant to Section 4.3, or by
the Company without Cause pursuant to Section 4.5, and provided that Executive (or Executive’s legal representative,
if  applicable)  executes  a  Release  and  the  Release  becomes  effective  and  irrevocable  prior  to  the  end  of  the  Review
Period,  that  number  of  Executive’s  unvested  stock  options  and  other  service-based  equity-based  awards  that  would
otherwise have vested from the effective date of Executive’s termination to the first anniversary of such date shall vest
as of the date the Release is effective and irrevocable and Executive (or Executive’s estate or legal representative, if
applicable) shall have until the earlier of the expiration date of the option or one (1) year from the date of termination
of Executive’s employment to exercise all vested options unless the stock plan pursuant to which the option is granted
requires  earlier  termination  in  connection  with  a  liquidation  or  sale  of  the  Company.    Any  equity  or  equity-based
awards  which  vest  based  upon  the  attainment  of  performance  measures  shall  be  governed  by  the  terms  of  the
applicable award agreement governing termination.  

(c)

In  the  event  Executive’s  employment  with  the  Company  is  terminated  by  the
Company  by  reason  of  non-renewal  of  the  Agreement  Term  pursuant  to  Sections  1  and  4.1,  by  Executive  for  Good
Reason pursuant to Section 4.3, or by the Company without Cause pursuant to Section 4.5, in any such case within
twelve (12) months following a Change in Control, in lieu of the acceleration provided for pursuant to Section 5.4(b)
above, provided that Executive (or Executive’s legal representative, if applicable) executes a Release and the Release
becomes effective and irrevocable prior to the end of the Review Period, to the extent vesting and acceleration will not
result in a violation of Section 409A, all of Executive’s unvested stock options and other service-based equity-based
awards then in effect shall vest as of the date the Release is effective and irrevocable and Executive (or Executive’s
estate or legal representative, if applicable) shall have until the earlier of the expiration date of the option or one (1)
year  from  the  date  of  termination  of  Executive’s  employment  to  exercise  all  vested  options  unless  the  stock  plan
pursuant  to  which  the  option  is  granted  requires  earlier  termination  in  connection  with  a  liquidation  or  sale  of  the
Company.  Any equity or equity-based awards which vest based upon the attainment of performance measures shall be
governed by the terms of the applicable award agreement governing termination following a Change in Control.  

(d)

In the event Executive’s employment with the Company is terminated by reason of
disability pursuant to Section 4.4, all unvested stock and stock options granted to Executive before and after the date of
this  Agreement  shall  be  immediately  forfeited  upon  the  effective  date  of  such  termination  of  employment  or  as
otherwise provided in the option agreement; provided, that, Executive shall have until the earlier of the expiration date
of the option or one (1) year from the date of termination of Executive’s employment to exercise all vested options
unless  the  stock  plan  pursuant  to  which  the  option  is  granted  requires  earlier  termination  in  connection  with  a
liquidation or sale of the Company.

Review  Period.    In  the  event  that  the  Review  Period  begins  in  one  taxable  year  of  the
Executive and ends in a later taxable year, any payments contingent upon Executive’s execution without revocation of
the Release prior to the end of the Review Period will commence to be paid (or as applicable, made in full) on the

5.5

Exhibit 10.21

first payroll date in the later taxable year.  In no event will any payments be made or commence to be paid later than
the ninetieth (90th) day following the Executive’s date of termination, subject to compliance with Section 12.6 herein.

5.6     Limitation on Benefits.  The Company will make the payments under this Agreement without
regard to whether the deductibility of such payments (or any other payments or benefits) would be limited or precluded
by Section 280G of the Internal Revenue Code of 1986, as amended (the “Code”) and without regard to whether such
payments  would  subject  Executive  to  the  federal  excise  tax  levied  on  certain  “excess  parachute  payments”  under
Section  4999  of  the  Code  (the  “Excise  Tax”);  provided,  however,  that  if  the  Total  After-Tax  Payments  (as  defined
below) would be increased by the reduction or elimination of any payment and/or other benefit (including the vesting
of  the  equity  awards)  under  this  Agreement,  then  the  amounts  payable  under  this  Agreement  will  be  reduced  or
eliminated as follows, if possible: (i) first, by reducing or eliminating any cash payments or other benefits (other than
the vesting of the equity awards) and (ii) second, by reducing or eliminating the vesting of those equity awards that
occur as a result of such Change in Control (as provided above), to the extent necessary to maximize the Total After-
Tax Payments. The Company’s independent, certified public accounting firm (the “Accounting Firm”) will determine
whether and to what extent payments or vesting under this agreement are required to be reduced in accordance with the
preceding  sentence.  For  purposes  of  this  Agreement,  “Total  After-Tax  Payments”  means  the  total  of  all  “parachute
payments” (as that term is defined in Section 280G(b)(2) of the Code) made to or for the benefit of Executive (whether
made  under  the  Agreement  or  otherwise)  by  the  Company  or  any  of  its  affiliates,  after  reduction  for  all  applicable
federal, state and local income taxes, employment, social security and  Medicare taxes, the imposition of the Excise
Tax and all other taxes, determined by applying the highest marginal rate under Section 1 of the Code and under state
and  local  laws  which  applied  (or  is  likely  to  apply)  to  the  Executive’s  taxable  income  for  the  tax  year  in  which  the
 transaction which causes the application of Section 280G of the Code occurs, or such other rate(s) as the Accounting
Firm  determines  to  be  likely  to  apply  to  the  Executive  in  the  relevant  tax  year(s)  in  which  any  of  the  parachute
payments are expected to be made. The Company agrees to pay for all costs associated with the Accounting Firm and
the  determination  of  the  payments  or  vesting  required  to  be  reduced  and  for  the  avoidance  of  doubt,  shall  not  be
required to pay any taxes, penalties, interest or other expenses to which Executive may be subject. If it is ultimately
determined (by IRS private letter ruling or closing agreement, court decision or otherwise) that Executive’s parachute
payments  were  reduced  by  too  much  or  by  too  little  in  order  to  accomplish  the  purpose  of  this  Section  5.6,  the
Executive  and  the  Company  shall  promptly  cooperate  to  correct  such  underpayment  or  overpayment  in  a  manner
consistent with the purpose of this Section 5.6.

5.7

Withholdings.  Payments made under this Section 5 shall be subject to applicable federal,
state and local taxes and withholdings.   If the payment of any COBRA or health insurance premiums would otherwise
violate the nondiscrimination rules or cause the reimbursement of claims to be taxable under the Patient Protection and
Affordable Care Act of 2010, together with the Health Care and Education Reconciliation Act of 2010 (collectively,
the “Act”) or Section 105(h) of the Code, the Company paid premiums shall be treated as taxable payments and be
subject to imputed income tax treatment to the extent necessary to eliminate any discriminatory treatment or taxation
under the Act or Section 105(h) of the Code.

6. Notices.    All  notices,  requests,  consents  and  other  communications  hereunder  will  be  in  writing,  will  be
addressed, if to the Company, at its principal corporate offices to the attention of the Legal Department, and if to Executive,
at his address set forth on the signature page hereto or in the personnel records of the Company (as applicable), or in either
case, such other address as a party may designate by notice hereunder, and will be either (i) delivered by hand, (ii) sent by
overnight  courier,  or  (iii)  sent  by  registered  or  certified  mail,  return  receipt  requested,  postage  prepaid.    All  notices,
requests, consents and other communications hereunder will be deemed to have been given either (i) if by hand, at the time
of the delivery thereof to the receiving party at the address of such party set forth above, (ii) if sent by overnight courier, on
the  next  business  day  following  the  day  such  notice  is  delivered  to  the  courier  service,  or  (iii)  if  sent  by  registered  or
certified mail, on the fifth business day following the day such mailing is made.

Exhibit 10.21

7. Absence  of  Restrictions.    Executive  represents  and  warrants  that  Executive  is  not  bound  by  any
employment contracts, restrictive covenants or other restrictions that prevent him from entering into employment with,
or carrying out his responsibilities for, the Company, or which are in any way inconsistent with any of the terms of this
Agreement.  Executive  further  represents  that,  except  as  Executive  has  previously  disclosed  or  described  to  the
Company, Executive is not bound by the terms of any agreement with any previous employer or other party to refrain
from using or disclosing any trade secret or confidential or proprietary information in the course of his employment
with the Company, to refrain from competing, directly or indirectly, with the business of such previous employer or
any  other  party,  or  to  refrain  from  soliciting  employees,  customers  or  suppliers  of  such  previous  employer  or  other
party.    Executive  further  represents  that  he  will  not  disclose  to  the  Company  or  induce  the  Company  to  use  any
confidential or proprietary information or material belonging to any previous employer or others.

8. Entire Agreement.  This Agreement constitutes the entire agreement between the parties and supersedes
all prior agreements and understandings, whether written or oral relating to the subject matter of this Agreement, with
the exception of the Invention, Non-Disclosure, Non-Competition and Non-Solicitation Agreement by and between the
Company and Executive. Notwithstanding the foregoing, the parties to this Agreement acknowledge that stock options
and other equity awards may be granted by the Company to Executive under and pursuant to the 2012 Plan and any
amendments thereto, as well as any additional plans, and the award agreements related to such plans.

9. Amendment.   This  Agreement  may  be  amended  or  modified  only  by  a  written  instrument  executed  by

both the Company and Executive.

10. Governing Law; Consent to Jurisdiction.  This Agreement shall be construed, interpreted and enforced in
accordance with the laws of the State of New York without regard to conflict of law principles.  Any action, suit or
other legal proceeding arising under or relating to any provision of this Agreement shall be commenced only in a court
of the County of New York, State of New York (or, if appropriate, a federal court located within the County of New
York,  State  of  New  York),  and  the  Company  and  Executive  each  consents  to  the  jurisdiction  of  such  a  court.    THE
COMPANY AND EXECUTIVE EACH HEREBY IRREVOCABLY WAIVE ANY RIGHT TO A TRIAL BY JURY
IN  ANY  ACTION,  SUIT  OR  OTHER  LEGAL  PROCEEDING  ARISING  UNDER  OR  RELATING  TO  ANY
PROVISION OF THIS AGREEMENT.

11. Successors and Assigns.  This Agreement shall be binding upon and inure to the benefit of both parties
and their respective successors and assigns, including any corporation or other entity with which, or into which, the
Company  may  be  merged  or  which  may  succeed  to  the  Company’s  assets  or  business,  provided, however,  that  the
obligations of Executive are personal and shall not be assigned by him.  Any purported assignment of this Agreement
by Executive shall be null and void. Notwithstanding the foregoing, if Executive dies the compensation and benefits
stated in this Agreement will be paid to his beneficiary or his estate if no beneficiary.

12. Miscellaneous.

12.1

No Waiver.    No  delay  or  omission  by  the  Company  in  exercising  any  right  under  this  Agreement
shall  operate  as  a  waiver  of  that  or  any  other  right.   A  waiver  or  consent  given  on  any  one  occasion  shall  be
effective only in that instance and shall not be construed as a bar or waiver of any right on any other occasion.

12.2

Captions.  The captions of the sections of this Agreement are for convenience of reference only and

in no way define, limit or affect the scope or substance of any section of this Agreement.

12.3

Severability.    In  case  any  provision  of  this  Agreement  shall  be  invalid,  illegal  or  otherwise
unenforceable, the validity, legality and enforceability of the remaining provisions shall in no way be affected or
impaired thereby.

12.4

Counterparts.  This Agreement may be executed in two or more counterparts, each of which shall be
deemed an original but all of which together shall constitute one and the same instrument. This Agreement may be
delivered by facsimile, and facsimile signatures shall be treated as original signatures for all applicable purposes.

Exhibit 10.21

12.5

Blue  Penciling.    To  the  extent  that  any  provision  herein  or  in  any  plan  of  nonqualified  deferred
compensation  that  this  document  is  a  part  of  contravenes  the  requirements  of  Code  Section  409A  (or  the
regulations thereunder), such provision shall be appropriately modified in accordance with available IRS guidance
(including  without  limitation  IRS  Notice  2010-6  and  related  guidance)  so  that  Executive  is  not  subject  to  the
adverse effects of Code Section 409A but will nevertheless retain, to the extent possible, the economic benefit of
the provision.  

12.6

Section 409A; Withholding. 

12.6.1
The payments under this Agreement are intended either to be exempt from Section 409A of
the  Code  under  the  short-term  deferral,  separation  pay,  or  other  applicable  exception,  or  to  otherwise
comply  with  Section  409A.    The  parties  agree  that  this  Agreement  shall  be  administered  in  a  manner
consistent with such intent.  For purposes of Section 409A, all payments under this Agreement shall be
considered separate payments.  If any amount or benefit payable to the Executive under this Agreement
upon  a  “termination  of  employment”  is  determined  by  the  Company  to  constitute  a  “deferral  of
compensation” for purposes of Section 409A (after taking into account any applicable exceptions), such
amount  or  benefit  shall  not  be  paid  or  provided  until  the  Executive  has  also  experienced  a  “separation
from service” from the Company within the meaning of Section 409A.  Notwithstanding any provision to
the contrary, to the extent Executive is considered a specified employee under Section 409A and would
be entitled during the six-month period beginning on Executive’s separation from service to a payment
that is not otherwise excluded under Section 409A, such payment will not be made until the earlier of the
six-month  anniversary  of  Executive’s  separation  from  service  or  death;  provided  that  the  first  payment
made  after  the  delay  shall  include  all  amounts  that  would  have  been  paid  earlier  but  for  such  six  (6)
month  delay.  At  the  request  of  the  Executive,  the  Company  shall  set  aside  those  payments  that  would
otherwise be made in such six-month period in a trust that is in compliance with Rev. Proc. 92-64.

12.6.2
If  an  expense  reimbursement  or  provision  of  in-kind  benefit  provided  to  the  Executive
under this Agreement is not exempt from Section 409A of the Code, the following rules apply: (i) in no
event shall any reimbursement be paid after the last day of the taxable year following the taxable year in
which the expense was incurred; (ii) the amount of reimbursable expenses incurred or provision of in-
kind benefits in one tax year shall not affect the expenses eligible for reimbursement or the provision of
in-kind benefits in any other tax year; and (iii) the right to reimbursement for expenses or provision of in-
kind benefits is not subject to liquidation or exchange for any other benefit.

12.6.3
The parties agree to negotiate in good-faith the amendment of this Agreement, as necessary,
to avoid any violations of Section 409A in a manner that preserves the original intent of the parties to the
extent reasonably possible. Notwithstanding the foregoing, the Company makes no representations that
the  payments  and  benefits  provided  under  this  Agreement  comply  with  Section  409A  and  in  no  event
shall the Company be liable for all or any portion of any taxes, penalties, interest or other expenses that
may be incurred by Executive on account of non-compliance with Section 409A.

12.6.4
withholdings.

All compensatory payments under this Agreement are subject to any required tax or other

12.7
Board committee.

Interpretation. References to decisions by the Company will be made by the Board or the applicable

 [signature page follows]

IN WITNESS WHEREOF, the parties hereto have executed this Agreement as of the day and year set first

forth above.

Exhibit 10.21

THE COMPANY:

INTERCEPT PHARMACEUTICALS, INC.

By: /s/ David Ford

Name: David Ford
Title: Chief Human Resources Officer

EXECUTIVE:

By: /s/ Jared Freedberg

Name: Jared Freedberg

Address for Notice Purposes:

[Last address in books and records of the Company]

Exhibit 10.21

Exhibit A

RELEASE OF CLAIMS1

FOR  AND  IN  CONSIDERATION  OF  the  payments  and  benefits  (the  “Separation  Benefits”)  to  be
provided to me in connection with the separation of my employment, in accordance with the Employment Agreement
between  Intercept  Pharmaceuticals,  Inc.  (the  “Company”)  and  me  dated  December  15th,  2020  (the  “Agreement”),
which Separation Benefits are conditioned on my signing this Release of Claims (“Release”) and which I will forfeit
unless I execute and do not revoke this Release of Claims, I, on my own behalf and on behalf of my heirs and estate,
voluntarily,  knowingly  and  willingly  release  and  forever  discharge  the  Company,  its  subsidiaries,  affiliates,  parents,
and,  in  their  capacities  as  such,      stockholders,  together  with  each  of  those  entities’  respective  officers,  directors,
stockholders,  employees,  agents,  fiduciaries  and  administrators,  each  in  their  capacities  as  such  (collectively,  the
“Releasees”) from any and all claims and rights of any nature whatsoever which I now have or in the future may have
against  them  up  to  the  date  I  execute  this  Release,  whether  known  or  unknown,  suspected  or  unsuspected.    This
Release includes, but is not limited to, any rights or claims relating in any way to my employment relationship with the
Company or any of the other Releasees or the termination thereof, any contract claims (express or implied, written or
oral),  including,  but  not  limited  to,  the  Agreement,  or  any  rights  or  claims  under  any  statute,  including,  without
limitation,  the  Americans  with  Disabilities  Act,  the  Age  Discrimination  in  Employment  Act,  the  Older  Workers’
Benefit  Protection  Act,  the  Rehabilitation  Act  of  1973  (including  Section  504  thereof),  Title  VII  of  the  1964  Civil
Rights  Act,  the  Civil  Rights  Act  of  1866  (42  U.S.C.  §  1981),  the  Civil  Rights  Act  of  1991,  the  Equal  Pay  Act,  the
National Labor Relations Act, the Worker Adjustment and Retraining Notification Act, the Family Medical Leave Act,
the Lilly Ledbetter Fair Pay Act, the Genetic Information Non-Discrimination Act, the New York State Human Rights
Law,  the  New  York  City  Human  Rights  Law,  and  the  Employee  Retirement  Income  Security  Act  of  1974,  all  as
amended, and any other federal, state or local law.  This Release specifically includes, but is not limited to, any claims
based  upon  the  right  to  the  payment  of  wages,  incentive  and  performance  compensation,  bonuses,  equity  grants,
vacation,  pension  benefits,  401(k)  Plan  benefits,  stock  benefits  or  any  other  employee  benefits,  or  any  other  rights
arising under federal, state or local laws prohibiting discrimination and/or harassment on the basis of race, color, age,
religion, sexual orientation, religious creed, sex, national origin, ancestry, alienage, citizenship, nationality, mental or
physical  disability,  denial  of  family  and  medical  care  leave,  medical  condition  (including  cancer  and  genetic
characteristics), marital status, military status, gender identity, harassment or any other basis prohibited by law.  

As a condition of the Company entering into this Release, I further represent that I have not filed against the
Company or any of the other Releasees, any complaints, claims or lawsuits with any arbitral tribunal, administrative
agency,  or  court  prior  to  the  date  hereof,  and  that  I  have  not  transferred  to  any  other  person  any  such  complaints,
claims or lawsuits.  I understand that by signing this Release, I waive my right to any monetary recovery in connection
with a local, state or federal governmental agency proceeding and I waive my right to file a claim seeking monetary
damages in any arbitral tribunal, administrative agency, or court.  This Release does not: (i) prohibit or restrict me from
communicating,  providing  relevant  information  to  or  otherwise  cooperating  with  the  U.S.  Equal  Employment
Opportunity Commission, the New York State Division of Human Rights, a local commission on human rights or any
other governmental authority with responsibility for the administration of fair employment practices laws (including
with respect to SEC Whistleblowing) or my own attorney regarding a possible violation of such laws or responding to
any inquiry from such authority, including an inquiry about the existence of this Release or its underlying facts, or (ii)
require  me  to  notify  the  Company  of  such  communications  or  inquiry.  Furthermore,  notwithstanding  the  foregoing,
this  Release  does  not  include  and  will  not  preclude:  (a)  rights  or  claims  to  vested  benefits  under  any  applicable
retirement  and/or  pension  plans;  (b)  rights  under  the  Consolidated  Omnibus  Budget  Reconciliation  Act  of  1985
(“COBRA”);  (c)  claims  for  unemployment  compensation;  (d)  rights  to  defense  and  indemnification  or  under  the
Company’s directors’ and officers’ liability insurance, if any, from the Company for actions or inactions taken by me
in the course and scope of my employment with the Company and its parents, subsidiaries and/or affiliates; (e) any
rights I may have to obtain contribution as permitted by law in the event of entry of judgment against the Company as
a result of any act or failure to act for which I and the Company are held jointly liable; (f) any rights to vested equity
that vested prior to or because of the termination of my employment and rights as a stockholder; and/or (g) any actions
to enforce the Agreement.

1

The  Executive  agrees  that  the  Company  may  revise  this  release  to  satisfy  the  purpose  of  providing  as  full  a  release  of  claims  (subject  to
payment of any benefits provided on the applicable termination of employment) as may be legally permissible.  The Company may revise it to
reflect changes in law for releases and may add language for ADEA compliance.

Exhibit 10.21

I  acknowledge  that,  in  signing  this  Release,  I  have  not  relied  on  any  promises  or  representations,
express or implied, other than those that are set forth expressly herein or in the Agreement and that are intended to
survive separation from employment, in accordance with the terms of the Agreement.

Nondisclosure; Continuing Obligations  -  I  understand  and  agree  that,  to  the  extent  permitted  by
law,  the  terms  and  contents  of  this  Release  (as  modified  before  signature)  and  the  contents  of  the  negotiations  and
discussions resulting in this Release shall be maintained as confidential by me and must not be disclosed to anyone
other than a member of my immediate family, my attorney, accountant or other advisor (and, even as to such a person,
only if the person agrees to honor this confidentiality requirement) except to the extent required by federal or state law
or as otherwise agreed to in writing by the Company.  I acknowledge and reaffirm my obligation to keep confidential
and not disclose any and all non-public information concerning the Company that I acquired during the course of my
employment or other relationship with the Company, including any non-public information concerning the Company’s
business affairs, business prospects and financial condition, as is stated more fully in any Invention, Non-Disclosure,
Non-Competition and Non-Solicitation Agreement and that I will comply with such agreement in all other respects.

The Company understands and agrees that the contents of the negotiations and discussions resulting
in this Release shall be maintained as confidential and shall not be disclosed to any third parties, except to the extent
required or permitted by applicable law or as otherwise agreed to in writing with you.

Pursuant to 18 U.S.C. § 1833(b), I understand that I will not be held criminally or civilly liable under
any  federal  or  state  trade  secret  law  for  the  disclosure  of  a  trade  secret  of  the  Company  that  (a)  is  made  (i)  in
confidence to a federal, state, or local government official, either directly or indirectly, or to my attorney and (ii) solely
for  the  purpose  of  reporting  or  investigating  a  suspected  violation  of  law;  or  (b)  is  made  in  a  complaint  or  other
document that is filed under seal in a lawsuit or other proceeding.  If I files a lawsuit for retaliation by the Company
for  reporting  a  suspected  violation  of  law,  I  may  disclose  the  trade  secret  to  my  attorney  and  use  the  trade  secret
information in the court proceeding, if I (a) file any document containing the trade secret under seal, and (b) do not
disclose  the  trade  secret,  except  pursuant  to  court  order.    Nothing  in  this  Agreement  is  intended  to  conflict  with  18
U.S.C. § 1833(b) or create liability for disclosures of trade secrets that are expressly allowed by such section.

Mutual Non-Disparagement – I understand and agree that I shall not make any false, disparaging
or  derogatory  statements  to  any  person  or  entity,  including  any  media  outlet,  industry  group  or  financial  institution,
regarding the Company, or any of the other Releasees or about the Company’s business affairs and financial condition.
 The Company confirms that it has instructed the members of its Board of Directors and its current executive officers
to  not  make  any  false,  disparaging  or  derogatory  statements  to  any  person  or  entity,  including  any  media  outlet,
industry  group  or  financial  institution,  regarding  me,  my  employment  with  the  Company,  or  my  departure  from  the
Company.  Notwithstanding the foregoing, nothing  herein  prevents  either  the  Releasees  or  me  from  making  truthful
disclosures  to  any  governmental  entity  or  to  enforce  the  Agreement  or  this  Release.    For  the  avoidance  of  doubt,
nothing  in  this  Release  prohibits  me  from  communicating  with  a  government  agency,  regulator  or  legal  authority
concerning any possible violations of federal or state law or regulation.  Nothing in this Release, however, authorizes
the  disclosure  of  information  I  obtained  through  a  communication  that  was  subject  to  the  attorney-client  privilege,
unless disclosure of the information would otherwise be permitted by an applicable law or rule.

Return of Company Property  -  I  confirm  that  I  have  returned  to  the  Company  in  good  working
order all Company-owned keys, files, records (and copies thereof), equipment (including computer hardware, software
and  printers,  wireless  handheld  devices,  cellular  phones,  tablets,  smartphones,  etc.),  Company  identification,  the
Company  proprietary  and  confidential  information,  and  any  other  Company-owned  property  in  my  possession  or
control and I have left intact with, or delivered intact to, the Company all electronic Company documents and internal
and external websites, including those that I developed or helped to develop during my employment, and that I have
thereafter  deleted,  and  destroyed  any  hard  copies  of,  all  electronic  files  relating  to  the  Company  that  are  in  my
possession or control, including any that are located on any of my personal computers or external or cloud storage.  I
further  confirm  that  I  have  cancelled  all  accounts  for  my  benefit,  if  any,  in  the  Company’s  name  including,  but  not
limited to, credit cards, telephone charge cards, cellular phone and/or wireless data accounts and computer accounts.
Notwithstanding the foregoing, I understand that I shall be permitted to retain my contacts and calendars and personal
correspondence  and  any  documents  or  data  related  to  my  compensation  or  reasonably  needed  for  tax  preparation
purposes.

in conjunction with my employment by the Company, including payment for all wages, bonuses, and equity for any

Final Compensation – I acknowledge that I have received payment in full for all services rendered

Exhibit 10.21

period before the date of this Release (other than any current salary and benefits due in the ordinary course in a final
paycheck or thereafter), and that no other compensation is owed to me, except as provided in the applicable provisions
of Section 5 of the Agreement; provided that nothing herein shall affect any claims of entitlement I may have to vested
benefits under any 401(k) plan or other ERISA-covered benefit plan (excluding severance) provided by the Company.

Cooperation  –  I  agree  to  cooperate  with,  provide  assistance  to,  and  make  myself  reasonably
available to the Company and its legal counsel in connection with any litigation (including arbitration or administrative
hearings) or investigation or examination relating to the Company or any of its current or former employees, in which,
in the reasonable judgment of the Company or its counsel, my assistance or cooperation is needed due to my personal
involvement in or knowledge about the circumstances to which the litigation or investigation relates. I will, when the
Company or its counsel requests, provide testimony, be available for interviews or other assistance and travel at the
Company’s reasonable request in order to fulfill this obligation. In connection with such litigation or investigation, the
Company will use its best efforts to accommodate my schedule, will provide me with as much notice as possible in
advance of the times during which my cooperation or assistance is needed, and will reimburse me for any reasonable
travel  and  lodging  expenses  incurred  in  connection  with  such  matters  (at  a  level  of  travel  consistent  with  my  travel
while employed by the Company) and the reasonable fees of any independent counsel retained by me if I reasonably
believe  separate  counsel  to  be  appropriate.  I  agree  not  to  assist  or  provide  information  to  any  adverse  party  in  any
litigation against the Company or any of its current or former employees, except as required under law or formal legal
process,  unless  I  provide  advance  notice  to  the  Company  at  least  10  days  before  such  assistance  or  provision  of
information (or, if I am so required to assist or provide such information within less than 10 days of receipt of such
requirement, after I provide timely advance notice to the Company) to allow the Company to take legal action with
respect to the matter.  Finally, I will undertake to satisfy requests for information from the Company with respect to the
above undertaking.  Nothing in this Release is intended to restrict or preclude me from, or otherwise influence me in,
testifying fully and truthfully in legal, administrative, or any other proceedings involving the Company, as required by
law or formal legal process.

Tax Provision – I acknowledge that I am not relying upon advice or representation of the Company
with respect to the tax treatment of any of the payments or benefits provided by the Company.  The benefits provided
to me are intended to be exempt from or compliant with Section 409A of the Internal Revenue Code of 1986.   The
Company makes no representation or warranty and shall have no liability to me or to any other person if any of the
provisions  of  the  Agreement  or  this  Release  are  determined  to  constitute  deferred  compensation  subject  to  Section
409A but not to satisfy an exemption for, or the conditions of, that section. All payments stated will be reduced by all
applicable taxes and withholdings.

not constitute an admission of liability or wrongdoing on the part of the Company.

Nature of Agreement – I understand and agree that this Release is a severance agreement and does

Voluntary Assent – I affirm that no other promises or agreements of any kind have been made to or
with me by any person or entity whatsoever to cause me to sign this Release, other than as reflected in the Agreement
and that I fully understand the meaning and intent of the Release. I acknowledge that, in signing this Release, I have
not relied on any promises or representations, express or implied, other than those that are set forth expressly herein or
in the Agreement and that are intended to survive separation from employment, in accordance with the terms of the
Agreement.  I further state and represent that I have carefully read this Release, understand the contents herein, freely
and voluntarily assent to all of the terms and conditions hereof, and sign my name of my own free act.

Validity  –  Should  any  provision  of  this  Release  be  declared  or  be  determined  by  any  court  of
competent  jurisdiction  to  be  illegal  or  invalid,  the  validity  of  the  remaining  parts,  terms  or  provisions  shall  not  be
affected thereby and said illegal or invalid part, term or provision shall be deemed not to be a part of this Release.

I further acknowledge that:

(1)

(2)

I first received this Release on the date of the Agreement to which it is attached as Exhibit
A;

I understand that, in order for this Release to be effective, I may not sign it prior to the date
of my separation of employment with the Company but that if I wish to receive the

Exhibit 10.21

Separation  Benefits,  I  must  sign  and  return  this  Release  prior  to  the  sixtieth  (60th)  day
following my separation of employment;  

I have carefully read and understand this Release;

The  Company  advised  me  to  consult  with  an  attorney  and/or  any  other  advisors  of  my
choice before signing this Release;

I understand that this Release is LEGALLY BINDING and by signing it I give up certain
rights;

I have voluntarily chosen to enter into this Release and have not been forced or pressured in
any way to sign it;

I  acknowledge  and  agree  that  the  Separation  Benefits  are  contingent  on  execution  of  this
Release,  which  releases  all  of  my  claims  against  the  Company  and  the  Releasees,  and  I
KNOWINGLY  AND  VOLUNTARILY  AGREE  TO  RELEASE  the  Company  and  the
Releasees  from  any  and  all  claims  I  may  have,  known  or  unknown,  in  exchange  for  the
benefits I have obtained by signing, and that these benefits are in addition to any benefit I
would have otherwise received if I did not sign this Release;

I have been given at least twenty-one (21) days to consider, and seven (7) days after I sign
this Release to revoke it by notifying the Company in writing.  The Release will not become
effective or enforceable until the seven (7) day revocation period has expired;

Any  revocation  of  this  release  must  be  made  in  a  signed  writing  and  sent  to  the  following
address no later than 5:00 PM on the seventh (7th) day after I have executed this Agreement:

[Address]

This Release  includes a WAIVER OF ALL RIGHTS AND CLAIMS I may have under
the Age Discrimination in Employment Act of 1967 (29 U.S.C. §621 et seq.); and

This Release does not waive any rights or claims that may arise after this Release becomes
effective, which is seven (7) days after I sign it, provided that I do not exercise my right to
revoke this Release.

(3)

(4)

(5)

(6)

(7)

(8)

(9)

(10)

(11)

Intending to be legally bound, I have signed this Release as of the date written below.

Signature: /s/ Jared Freedberg
Jared Freedberg

December 21, 2020
   Date signed

EX-10.39 3 v451028_ex10-39.htm EXHIBIT 10.39

Exhibit 10.39

Execution Version

Certain identified information has been excluded from this exhibit because it is both not 
material and would likely cause competitive harm to the registrant if publicly disclosed.

MANUFACTURING AND SUPPLY AGREEMENT

between

INTERCEPT PHARMA EUROPE LTD.

and

PHARMAZELL GMBH

ARTICLE 1

DEFINITIONS

ARTICLE 2

MANUFACTURING AND SUPPLY

2.1

2.2

2.3

2.4

2.5

2.6

2.7

Supply Obligations

Work Orders

Delivery Terms; Inspection

Materials

Costs and Expenses

Supply Shortage; Inability to Supply

Intercept Materials

ARTICLE 3

QUALITY; COMPLIANCE; REGULATORY

3.1

3.2

3.3

3.4

3.5

3.6

3.7

Quality Control

Maintenance of Facility

Regulatory Cooperation of PharmaZell

Cooperation with Regulatory Authorities and Regulatory Correspondence

Compliance with Applicable Law

Change Requests

General Cooperation

ARTICLE 4

FINANCIALS

4.1

4.2

4.3

4.4

4.5

Price

Invoice and Payment

Currency

Adjustment of Purchase Price

Audit; Late Payments

ARTICLE 5

INTELLECTUAL PROPERTY

5.1

5.2

5.3

5.4

5.5

5.6

Ownership of Inventions

Patent Prosecution

Enforcement of Patents

Third Party Litigation

Third Party Licenses

United States Law

ARTICLE 6

REPRESENTATIONS AND WARRANTIES; COVENANTS

6.1

6.2

Representations and Warranties of Each Party

Additional Representations, Warranties and Covenants of PharmaZell

-i-

1

7

7

8

10

10

11

11

11

13

13

14

15

15

16

16

16

17

17

17

18

18

19

20

20

22

24

25

25

25

26

26

26

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
6.3

Disclaimer of Other Warranties

ARTICLE 7

CONFIDENTIALITY

7.1

7.2

7.3

7.4

7.5

7.6

7.7

Confidential Information

Exceptions to Confidentiality

Disclosure

Notification

Remedies

Use of Names

Press Releases

ARTICLE 8

TERM AND TERMINATION

8.1

8.2

8.3

Term

Termination

Effect of Expiration or Termination

ARTICLE 9

INDEMNIFICATION

9.1

9.2

9.3

9.4

9.5

PharmaZell Indemnification

Intercept Indemnification

Indemnification Procedure

Insurance

Limitation on Damages

ARTICLE 10

MISCELLANEOUS

10.1

Notices

10.2

Force Majeure

10.3

Entire Agreement; Amendment

10.4

Further Assurances

10.5

Successors and Assigns

10.6

Governing Law

10.7

Dispute Resolution

10.8

Arbitration

10.9

Third Party Beneficiaries

10.10

Export Control

10.11

Assignment

10.12 Waiver

10.13

Severability

-ii-

28

28

28

28

29

29

29

30

30

30

30

30

31

33

33

33

33

35

35

36

36

37

37

38

38

38

38

38

40

40

40

41

41

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
10.14

Independent Contractors

10.15

Construction

10.16

Remedies

10.17

Counterparts; Facsimile Execution

10.18

English Language

10.19

Parent Guarantee

-iii-

41

41

41

42

42

42

 
 
 
 
 
 
 
 
 
 
This MANUFACTURING AND SUPPLY AGREEMENT (this “Agreement”), dated the last date of signature (the “Effective
Date”),  is  made  by  and  between  Intercept  Pharma  Europe  Ltd.,  having  a  location  at  2  Pancras  Square,  Floor  1,  London,  United
Kingdom N1C 4AG (“Intercept”), and, solely for purposes of Section 10.19, Intercept Pharmaceuticals, Inc. (“Intercept Parent”), and
PharmaZell  GmbH,  a  corporation  organized  under  the  laws  of  Germany  (“PharmaZell”).  Intercept  and  PharmaZell  are  sometimes
referred to herein individually as a “Party” and collectively as the “Parties.”

RECITALS

WHEREAS,  pursuant  to  a  certain  Development  Agreement  by  and  between  the  Parties  dated  August  18,  2010,  the  Parties
collaborated to develop a synthesis pathway for the manufacture, production, and validation of an active pharmaceutical ingredient for
Intercept referred to as [**]; and

WHEREAS, Intercept and PharmaZell now wish to enter into this Agreement to arrange for the manufacture and supply by

PharmaZell to Intercept of the API (as defined below), on the terms and subject to the conditions set forth in this Agreement.

NOW, THEREFORE, in consideration of the foregoing premises, the mutual promises and covenants of the Parties contained
herein, and other good and valuable consideration, the receipt and sufficiency of which are hereby acknowledged, the Parties, intending
to be legally bound, do hereby agree as follows:

ARTICLE 1
DEFINITIONS

As used herein, the following terms shall have the following meanings:

1.1         “Adjustment Date” has the meaning set forth in Section 4.4(a).

1.2         “Adverse Event” means (a) any finding from tests in laboratory animals or in vitro that suggests a significant risk for
human subjects including reports of mutagenicity, teratogenicity or carcinogenicity, (b) any undesirable, untoward or noxious event or
experience  associated  with  the  clinical,  commercial  or  other  use,  or  occurring  following  application  of  a  Product  to  humans,  whether
expected and whether considered related to or caused by such Product, including such an event or experience as occurs in the course of
the use of such Product in professional practice, in a clinical trial, whether accidental or intentional, from abuse, from withdrawal or from
a  failure  of  expected  therapeutic  action  of  such  Product,  and  (c)  those  events  or  experiences  that  are  required  to  be  reported  to  the
Regulatory Authorities under corresponding Applicable Law.

1.3         “Affiliate” of a Person means any other Person that directly, or indirectly through one or more intermediaries, controls,
is  controlled  by  or  is  under  common  control  with,  such  first  Person.  For  purposes  of  this  definition,  “control”  and,  with  correlative
meanings, the terms “controlled by” and “under common control with”, means to possess the power to direct the management or policies
of a Person, whether through ownership of voting securities or by contract or otherwise.

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1.4         “Agreement” has the meaning set forth in the preamble hereto, including all Work Orders provided by Intercept.

1.5         “API” means the active pharmaceutical ingredient [**].

1.6         “API Precursor” means any intermediary, ingredient, composition or element [**] that arises or is created or produced

following production of the Intermediary during the Manufacture of the API.

1.7         “API Specifications” means the specifications for the API to be Manufactured by PharmaZell and supplied to Intercept

hereunder as such specifications are set forth in the Quality Agreement, as the same may be amended from time to time.

1.8         “Applicable Law” means all laws, statutes, rules, codes, regulations, requirements, orders, judgments and ordinances

of any Regulatory Authority, including the FFDCA.

1.9         “Business Day” means a day other than a Saturday or a Sunday on which banks in New York, New York and Munich,

Germany are open for the conduct of regular banking business.

1.10       “Calendar Quarter” means each period of three (3) consecutive calendar months commencing on 1 January, 1 April, 1
July, and 1 October, except that the first Calendar Quarter of the Term shall commence on the Effective Date and end on September 30,
2016, and the last Calendar Quarter of the Term shall commence on the first day of the calendar quarter in which the Term ends and end
on the last day of the Term.

1.11       “Calendar Year” means each successive period of twelve (12) consecutive calendar months commencing on 1 January
and  ending  on  31  December,  except  that  the  first  Calendar  Year  of  the  Term  shall  commence  on  the  Effective  Date  and  end  on  31
December 2016, and the last Calendar Year of the Term shall commence on January 1 of the year in which the Term ends and end on the
last day of the Term.

1.12       “Certificate of Analysis” or “COA” has the meaning set forth in the Quality Agreement.

1.13       “Certificate of Compliance” or “COC” has the meaning set forth in the Quality Agreement.

1.14       “CMC Data” means the chemistry, manufacturing and controls data required by Applicable Law to be included in a
New Drug Application (as defined in the FFDCA and the regulations promulgated thereunder) for a Product or in any other Regulatory
Approval outside the United States.

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1.15       “Confidential Information” means any and all information or material that, at any time before or after the Effective
Date, has been or is provided or communicated to the Receiving Party by or on behalf of the Disclosing Party (including by a third party)
pursuant to this Agreement or in connection with the transactions contemplated hereby or any discussions or negotiations with respect
thereto; any data, ideas, concepts or techniques contained therein; and any modifications thereof or derivations therefrom. Confidential
Information  may  be  disclosed  either  orally,  visually,  electronically,  in  writing,  by  delivery  of  Materials  containing  Confidential
Information or in any other form now known or hereafter invented.

1.16       “Control” means, with respect to any item of information, Invention, Regulatory Documentation, patent, trademark or
other intellectual property right, possession of the right, whether directly or indirectly, and whether by ownership, license or otherwise
(other than by operation of any license and other grants hereunder), to assign or grant a license, sublicense or other right to or under, or
perform other acts in respect of, such information, Invention, Regulatory Documentation, patent, trademark or other intellectual property
right as provided for herein without violating the terms of any agreement or other arrangement with any third party.

1.17       “Deficiency” has the meaning set forth in Section 2.3(c).

1.18       “Delivery Date” means the date the API leaves the Facility for shipment to Intercept.

1.19       “Disclosing Party” means the Party disclosing Confidential Information.

1.20       “Disqualification” has the meaning set forth in Section 6.2(c).

1.21       “Effective Date” has the meaning set forth in the preamble hereto.

1.22       “Employee Inventions” has the meaning set forth in Section 5.1(g).

1.23       “Existing Work Orders” has the meaning set forth in Section 2.2(a).

1.24       “Exploit” means to make, have made, import, use, sell, offer for sale or otherwise dispose of a compound, product or
process,  including  all  discovery,  research,  development,  commercialization,  registration,  modification,  enhancement,  improvement,
Manufacture, storage, formulation, optimization, exportation, transportation, distribution, promotion and marketing of such compound,
product or process.

1.25       “Facility” means a Manufacturing facility of PharmaZell located at (i) [**], (ii) [**], and/or (iii) such other facility as

the Parties may agree to in writing from time to time.

1.26       “FDA” means the United States Food and Drug Administration and any successor agency thereto.

1.27              “FFDCA”  means  the  U.S.  Federal  Food,  Drug,  and  Cosmetic  act  codified  at  21  U.S.C.  §  301  et  seq.,  as  may  be

amended from time to time.

1.28       “Gesetz über Arbeitnehmererfindungen” has the meaning set forth in Section 5.1(g).

1.29              “GMI”  means  the  German  Producer  Price  Index  (“Index  der  Erzeugerpreise  gewerblicher  Produkte”)  for
pharmaceutical preparations, as compiled and published by the Bureau of Labor Statistics of the United States Department of Labor and
using the latest version of data published as of the date of adjustment.

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1.30       “GMP” or “cGMP” means all applicable standards relating to manufacture of pharmaceutical products, including, as
applicable  current  Good  Manufacturing  Practices  as  they  apply  to  the  manufacture  of  Supplied  Material,  and  including  (i)  standards
promulgated by any Regulatory Authority having jurisdiction over the Manufacture of the Supplied Material, in the form of Applicable
Laws, including the U.S. current Good Manufacturing Practices regulations promulgated by the FDA, as described in 21 U.S.C. 351, 21
C.F.R.  Parts  210  and  211,  as  amended,  and  any  successor  provision  thereto  and  ICH  Q7  –  Good  Manufacturing  Practice  for  Active
Pharmaceutical  Ingredients;  (ii)  standards  promulgated  by  any  Regulatory  Authority  having  jurisdiction  over  the  Manufacture  of  the
Supplied  Material,  in  the  form  of  draft  or  final  guidance  documents  (including  advisory  opinions,  compliance  policy  guides  and
guidelines); and (iii) such other industry standards as may be agreed upon by the Parties in the Specifications (as defined and set forth in
the Quality Agreement).

1.31       “ICC Rules” has the meaning set forth in Section 10.8(a).

1.32       “Indemnification Claim Notice” has the meaning set forth in Section 9.3(a).

1.33       “Indemnified Party” has the meaning set forth in Section 9.3(a).

1.34       “Indemnifying Party” has the meaning set forth in Section 9.3(a).

1.35       “Initial Term” has the meaning set forth in Section 8.1.

1.36       “Intercept” has the meaning set forth in the preamble hereto.

1.37       “Intercept Indemnified Parties” has the meaning set forth in Section 9.1.

1.38              “Intercept  Information”  means  all  technical,  scientific  and  other  know-how  and  information,  trade  secrets,
knowledge, technology, means, methods, processes, practices, formulae, instructions, skills, techniques, procedures, technical assistance,
designs,  assembly  procedures,  specifications,  assays,  test  methods,  analytical  methods,  and  other  material  or  information  owned  or
Controlled by Intercept or its Affiliates (including information received from a third party) as of the Effective Date or at any time during
the Term.

1.39       “Intercept Intellectual Property” has the meaning set forth in Section 5.1(a).

1.40       “Intercept Materials” means those Materials identified on Schedule 1.40 to be supplied by Intercept to PharmaZell for

Manufacture of the API.

1.41       “Intermediary” means [**].

1.42              “Invention”  means  any  discovery,  improvement,  process,  formula,  data,  information,  invention,  know-how,  trade
secret, procedure, device, or other intellectual property, whether or not protectable under patent, trademark, copyright or similar laws,
including  any  enhancement  in  the  manufacture,  formulation,  ingredients,  preparation,  presentation,  means  of  delivery,  dosage  or
packaging of a compound or product or any discovery or development of a new indication for a compound or product.

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1.43       “Joint Invention Patents” has the meaning set forth in Section 5.2(c)(i).

1.44       “Joint Inventions” mean any and all Inventions that are or have been created, conceived, discovered, developed or

otherwise made jointly by or on behalf of the Parties, but excluding Specified Inventions.

1.45              “Latent Defect”  means  any  deficiency  (including  any  Supplied  Material  that  fails  to  meet  the  Supplied  Material
Warranty or other quality requirements set forth in the Quality Agreement) that is not readily determinable upon a reasonable inspection
of the Supplied Material (based on physical inspection, identity test and review of the certificate of analysis).

1.46       “Losses” has the meaning set forth in Section 9.1.

1.47              “Manufacture”  and  “Manufacturing”  means  all  steps,  processes,  activities  and  operations  from  purchase  of

Materials, through production, quality control, release and storage, to distribution of API, and the related controls.

1.48       “Material(s)” means all ingredients, raw materials, packaging and labeling components, and all other supplies of any

kind, required or used in connection with the Manufacturing of Supplied Material.

1.49       “Minimum Annual Requirement” has the meaning set forth in Section 2.2(b).

1.50       “Minimum Percentage Requirement” has the meaning set forth in Section 2.2(b).

1.51       “Other PharmaZell Invention Patents” has the meaning set forth in Section 5.2(b)(i).

1.52       “Other PharmaZell Inventions” means [**].

1.53       “Party” and “Parties” has the meaning set forth in the preamble hereto.

1.54              “Person”  means  an  individual,  sole  proprietorship,  partnership,  limited  partnership,  limited  liability  partnership,
corporation,  limited  liability  company,  business  trust,  joint  stock  company,  trust,  unincorporated  association,  joint  venture  or  other
similar entity or organization, including a government or political subdivision, department or agency of a government.

1.55       “PharmaZell” has the meaning set forth in the preamble hereto.

1.56       “PharmaZell Indemnified Parties” has the meaning set forth in Section 9.2.

1.57       “Policies” has the meaning set forth in Section 9.4(a).

1.58       “Products” means the finished product containing the API.

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1.59       “Purchase Price” has the meaning set forth in Section 4.1(a).

1.60       “Quality Agreement” means the quality assurance agreement dated August 20, 2014 entered into by the Parties.

1.61       “Quality Standards” means the obligations set forth in the Quality Agreement as well as compliance with applicable

environmental/health/safety requirements and cGMP requirements.

1.62       “Receiving Party” means the Party receiving Confidential Information.

1.63       “Recipients” has the meaning set forth in Section 7.1.

1.64       “[**]” means [**].

1.65       “Regulatory Approval” means, with respect to any particular country or other jurisdiction, as applicable any and all
approvals,  licenses,  registrations  or  authorizations  of  any  Regulatory  Authority  necessary  for  the  Exploitation  of  a  Product  in  such
country or jurisdiction, including, where applicable, (a) approval of a Product in such country or jurisdiction, including any marketing
authorization and supplements and amendments thereto, including an approved New Drug Application as defined in the FFDCA or any
corresponding  foreign  application,  registration  or  certification  necessary  or  reasonably  useful  to  market  any  Product  in  a  country  or
regulatory  jurisdiction;  (b)  pre-  and  post-approval  marketing  authorizations  (including  any  prerequisite  Manufacturing  approval  or
authorization related thereto); (c) labeling approval; and (d) technical, medical and scientific licenses.

1.66              “Regulatory Authority”  means  any  applicable  supra-national,  federal,  national,  regional,  state,  provincial  or  local
regulatory  agencies,  departments,  bureaus,  commissions,  councils  or  other  government  entities  regulating  or  otherwise  exercising
authority  with  respect  to  the  Exploitation  of  Supplied  Material  or  a  product  in  any  country  or  other  jurisdiction,  including  those
responsible for granting approvals for the performance of services by PharmaZell to Intercept or for issuing regulations pertaining to the
manufacture or use of the Supplied Material or Product in the intended country of use, including the FDA.

1.67              “Regulatory  Documentation”  means  as  applicable  (a)  submissions  to  any  Regulatory  Authority,  including
investigational new drug applications, New Drug Applications (as defined in the FFDCA and the regulations promulgated thereunder),
correspondence  with  regulatory  agencies  (registrations  and  licenses,  regulatory  drug  lists,  advertising  and  promotion  documents),
periodic  safety  update  reports,  adverse  event  files,  complaint  files  and  manufacturing  records  and,  if  applicable,  any  updates  or
supplements to any of the foregoing and (b) any minutes or contact logs with respect to any telephone conferences or in-person meetings
conducted with any Regulatory Authority relating to the subject matter described in clause (a) of this sentence.

1.68              “Release  Testing”  means  all  testing  of  the  quality  attributes  of  the  Supplied  Material  in  accordance  with  the

Specifications and the Quality Agreement.

1.69       “Renewal Period” has the meaning set forth in Section 8.1.

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1.70       “Required Manufacturing Changes” has the meaning set forth in Section 3.6(b).

1.71       “Representative” has the meaning set forth in Section 6.2(a).

1.72       “Services” means the Manufacturing, supply and other services performed under this Agreement.

1.73       “Specifications” means the API Specifications.

1.74       “Specified Invention Patents” has the meaning set forth in Section 5.2(a)(i).

1.75       “Specified Inventions” means [**].

1.76       “Supplied Material” means the API.

1.77       “Supplied Material Warranty” has the meaning set forth in Section 6.2(b).

1.78       “Term” has the meaning set forth in Section 8.1.

1.79       “Testing Laboratory” means an independent third party laboratory engaged by the Parties to test conformance of the

Supplied Material to the Specifications in accordance with the terms set forth in the Quality Agreement.

1.80       “Third Party Claim” has the meaning set forth in Section 9.1.

1.81       “Total Commercial Volume Requirements” means, for purposes of calculating Intercept’s total commercial volume

requirements for Supplied Material for a given Calendar Year, the total amount of Supplied Material [**].

1.82       “United States” means the United States of America, its territories and possessions, including the District of Columbia

and Puerto Rico.

1.83       “Work Order” means a written work order that sets forth, with respect to the period covered thereby, (a) the quantities
of  each  Supplied  Material  to  be  processed  and  delivered  by  PharmaZell  to  Intercept  or  its  designee,  (b)  the  required  Delivery  Dates
therefor, and (c) the required delivery locations therefor, in the form attached hereto as Schedule 1.83.

ARTICLE 2
MANUFACTURING AND SUPPLY

2.1         Supply Obligations.

(a)          Generally. Subject to the terms and conditions hereof, PharmaZell shall Manufacture and supply to Intercept
such quantities of Supplied Material as Intercept may from time to time during the Term order. Such Manufacture and supply shall be in
accordance  with  Applicable  Laws,  the  Specifications,  the  Regulatory  Documentation,  Regulatory  Approvals  and  the  terms  of  this
Agreement and the Quality Agreement.

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(b)          Exclusivity of PharmaZell. To the maximum extent permitted by Applicable Law, without the written consent
of Intercept, PharmaZell shall not, and PharmaZell shall cause its Affiliates not to, distribute, market, promote, offer for sale, sell, supply
or Manufacture API or any API Precursor, directly or indirectly, whether alone or in combination with other molecules or compounds,
whether as a raw material or as a finished product, and whether at wholesale or retail, to any Person other than Intercept, its Affiliates or
designees.

(c)                    Purchase  Obligations  of  Intercept.  Subject  to  the  Minimum  Percentage  Requirement  and  the  Minimum
Annual  Requirement  set  forth  in  Section  2.2(b),  this  Agreement  shall  not  limit  Intercept’s  right  to  obtain  Supplied  Material  from  any
third  party.  PharmaZell  acknowledges  that  Intercept  has  the  right  to  enter  into  arrangements  with  one  or  more  third  parties  to  act  as
additional sources of Supplied Material.

(d)                    Subcontractors.  PharmaZell  may  not  subcontract  with  any  third  party  to  perform  any  of  its  obligations
hereunder without the prior written consent of Intercept; provided that with respect to the existing subcontractors and activity set forth
on Schedule 2.1(d),  Intercept  hereby  agrees  that  such  subcontractors  are  hereby  permitted  subcontractors  with  respect  to  the  activity
identified  for  such  subcontractor.  PharmaZell  shall  be  solely  responsible  for  the  performance  of  any  permitted  subcontractor,  and  for
costs,  expenses,  damages,  or  losses  of  any  nature  arising  out  of  such  performance  as  if  such  performance  had  been  provided  by
PharmaZell itself under this Agreement. PharmaZell shall cause any such permitted subcontractor to be bound by, and to comply with, all
confidentiality,  quality  assurance,  regulatory  and  other  obligations  and  requirements  of  PharmaZell  set  forth  in  this  Agreement.
PharmaZell and its subcontractors may use Intercept Intellectual Property only for the performance of the Services as specified in this
Agreement.

2.2         Work Orders.

(a)          Existing Work Orders. The Parties acknowledge and agree that Intercept and PharmaZell have, prior to the
date  hereof,  agreed  to  certain  Work  Orders  with  respect  to  Supplied  Materials,  including  penalties  therein  for  PharmaZell’s  failure  to
deliver Supplied Material in accordance with the terms of such Work Orders. The existing Work Orders are attached hereto as Schedule
2.2(a) (the “Existing Work Orders”). The Parties acknowledge and agree that PharmaZell shall continue to Manufacture the quantities
of  Supplied  Materials  set  forth  in  the  Existing  Work  Orders  in  accordance  with  the  timelines  set  forth  in  the  Existing  Work  Orders;
provided, however, the Parties acknowledge and agree that the Supplied Materials Manufactured and supplied under the Existing Work
Orders  shall  be  governed  by  the  terms  and  conditions  of  this  Agreement,  and  this  Agreement  supersedes  and  replaces  any  term  or
condition contained in such Existing Work Orders and any term or condition associated with such Existing Work Orders other than the
delivery  obligations,  the  price,  the  shared  risk  provisions  and  associated  penalties  of  PharmaZell,  which  shall  continue  to  apply  as
specified in the Existing Work Orders.

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(b)          New Work Orders; Minimum Percentage Requirement. Intercept shall place Work Orders at least [**] months
in advance of the requested Delivery Date but no more than [**] months in advance of the requested Delivery Date. With respect to each
Work  Order,  Intercept  shall  be  obligated  to  purchase,  and  PharmaZell  shall  be  obligated  to  deliver,  by  the  required  Delivery  Date  set
forth therein such quantities of the Supplied Material as are set forth therein. Intercept agrees to order from PharmaZell at least [**] of
Intercept’s Total Commercial Volume Requirements for delivery in each of [**] (“Minimum Percentage Requirement”); provided that,
[**]  notwithstanding  Intercept’s  actual  Total  Commercial  Volume  Requirements  in  Calendar  Years  2017  and  2018,  at  a  minimum,
Intercept  shall  order  at  least  [**]  of  Supplied  Material  to  be  delivered  in  each  of  Calendar  Year  2017  and  Calendar  Year  2018
(“Minimum Annual Requirement”). Notwithstanding the foregoing, (i) to the extent that Intercept has ordered a quantity of Supplied
Material from PharmaZell but PharmaZell fails for any reason to deliver such quantity within [**] days of the Delivery Date or such
Supplied  Material  is  rejected  by  Intercept  pursuant  to  Section  2.3(c),  all  such  ordered  Supplied  Material  shall  be  considered  Supplied
Material that was “ordered and delivered” under the terms of this Section 2.2(b) in calculating the Minimum Percentage Requirement
and  Minimum  Annual  Requirement,  and  (ii)  if  Intercept’s  Total  Commercial  Volume  Requirements  in  a  given  year  are  in  excess  of
PharmaZell’s capacity to Manufacture such quantity of Supplied Material, then for purposes of calculating Intercept’s total volume, the
percentage shall be based upon PharmaZell’s maximum capacity. In addition, if Intercept has ordered a quantity of Supplied Material
from PharmaZell but PharmaZell fails to deliver such quantity as a result of PharmaZell’s inability to satisfy the Quality Standards (and
PharmaZell is unable to remedy such inability to satisfy the Quality Standards within [**] days) or the Supplied Material is rejected by
Intercept pursuant to Section 2.3(c) as a result of PharmaZell’s failure to satisfy the Quality Standards, then (i) Intercept’s obligation to
achieve the Minimum Percentage Requirement and Minimum Annual Requirement shall be suspended until such time as PharmaZell is
able to remedy such Quality Standard issue and (ii) Intercept’s Minimum Percentage Requirement and Minimum Annual Requirement
for such Calendar Year shall be proportionately reduced by the length of the suspension; provided that if PharmaZell is able to remedy
the issue with the Quality Standards and deliver Supply Material to Intercept and Intercept accepts the full amount of the delivery despite
the  proportional  reduction,  then  Intercept’s  Minimum  Annual  Requirement  and  Minimum  Percentage  Requirement  for  the  subsequent
Calendar  Year  shall  be  reduced  by  such  proportionate  amount.  To  the  extent  PharmaZell  is  responsible  for  manufacturing  the
Intermediary  and  to  the  extent  Intercept  is  responsible  for  supplying  the  [**]  to  PharmaZell  for  the  manufacture  of  the  Intermediary,
Intercept shall ensure timely delivery of the [**] to PharmaZell. In addition, in the event that [**], then Intercept shall have no Minimum
Annual Requirement commencing on the date of any such event and for the duration of the Agreement. The Parties agree that the first
new work order under the Agreement shall be as specified in Schedule 2.2(b) attached hereto.

(c)          Work Order Terms. In the event that the terms of any Work Order are not consistent with or are in addition to
the terms of this Agreement, the terms of this Agreement shall prevail. The Parties agree that each Work Order shall be for a minimum of
[**] and that Intercept shall attempt to order a batch size of [**]. The Parties further agree that if the Manufacturing is to be done at [**],
the size of the batch in a Work Order [**] but otherwise is subject to the terms of this Agreement.

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2.3         Delivery Terms; Inspection.

(a)          Delivery. PharmaZell shall deliver the quantities of API set forth in each Work Order by the required Delivery
Date(s) set forth in such Work Order and in accordance with the reasonable written instructions as such instructions are agreed by the
Parties. PharmaZell shall deliver API, DAP (Incoterms 2010), with the delivery address specified by Intercept. Risk of loss and title shall
pass to Intercept upon delivery of API as specified in the preceding sentence. In the event Intercept wishes to have an expedited delivery,
PharmaZell reserves the right to charge Intercept for the additional costs involved therefor.

(b)          Accompanying Documentation. Each delivery of API shall be accompanied by (i) a Certificate of Analysis,
(ii)  a  Certificate  of  Compliance,  (iii)  such  other  documents  as  may  be  required  pursuant  to  the  Quality  Agreement,  and
(iv) documentation necessary for the sale or export of the API, as applicable.

(c)          Inspection. Within [**] days of receipt of a given shipment of Supplied Material, Intercept (or its agent) shall
verify on the basis of a visual inspection the quantity of Supplied Material delivered. In addition, Intercept (or its agent) shall inspect at
Intercept’s discretion (based minimally on physical inspection, identity test and review of the Certificate of Analysis and Certificate of
Conformance provided by PharmaZell) the Supplied Material following Delivery for variances and defects; and if Intercept claims that a
shipment  of  Supplied  Material  did  not,  at  the  time  of  receipt  by  Intercept,  meet  the  Supplied  Material  Warranty  or  the  quality
requirements set forth in the Quality Agreement (a “Deficiency”), Intercept shall notify PharmaZell based on the foregoing inspection
within [**] days after receipt of such Supplied Material at Intercept’s (or its designee’s) site, which notice shall provide the quantities
affected,  the  basis  for  the  claim  and  other  information  reasonably  necessary  for  PharmaZell  to  assess  the  claim.  Notwithstanding  the
foregoing, if Intercept claims that the Deficiency is a Latent Defect, Intercept shall have the obligation to provide such notification to
PharmaZell in writing within [**] days after Intercept’s discovery of such Latent Defect (or within [**] days after Intercept is notified in
writing  by  a  third  party  of  such  Latent  Defect,  if  later).  If  Intercept  and  PharmaZell  are  unable  to  agree  as  to  whether  such  Supplied
Material contains a Deficiency, the Parties shall cooperate to have the Supplied Materials in dispute analyzed by the Testing Laboratory.
The results of the Testing Laboratory shall be final and binding on the Parties on the issue of whether such Supplied Material contains a
Deficiency.  If  the  Supplied  Materials  are  determined  to  not  contain  a  Deficiency,  then  Intercept  shall  bear  the  cost  of  the  Testing
Laboratory  and  pay  the  Purchase  Price  with  respect  to  the  Supplied  Materials  in  accordance  with  this  Agreement.  If  the  Supplied
Materials are determined to contain a Deficiency, then PharmaZell shall bear the cost of the Testing Laboratory, and PharmaZell shall (i)
at Intercept's election, either replace the rejected Supplied Materials at no cost to Intercept, or refund to Intercept the Purchase Price paid
for such Supplied Materials, and the cost of all Intercept Materials used for such Supplied Materials plus any applicable delivery charge
and  (ii)  reimburse  to  Intercept  all  costs  associated  with  any  manufacturing  and  distribution  of  Products  incorporating  such  Supplied
Material, including formulation, packaging, storage and distribution expenses (and including materials used in connection therewith).

2.4                  Materials.  PharmaZell  shall  be  responsible  for  auditing  and  qualifying  its  supplier(s)  of  Materials  and  obtaining
supplies of Materials in accordance with the Specifications, Applicable Laws, Regulatory Documentation, Regulatory Approvals and the
Quality Agreement. Quality and Regulatory and all GMP related issues shall be defined in the Quality Agreement. At all times during the
Term,  PharmaZell  shall  (at  its  own  cost  and  expense)  maintain  sufficient  amounts  of  available  inventory  of  Materials  (other  than
Intercept Materials) consistent with industry standards and shelf life requirements of such Materials as may be necessary for PharmaZell
to Manufacture Supplied Materials.

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2.5         Costs and Expenses. Except as otherwise explicitly set forth herein, PharmaZell shall be solely responsible for all costs
and expenses incurred in connection with the Manufacture of Supplied Materials hereunder, including costs and expenses of personnel,
quality control testing, Manufacturing facilities and equipment, and Materials. In addition, at PharmZell’s cost and expense, PharmaZell
shall be entitled to maintain an inventory of safety stock of Supplied Material and any of its intermediates.

2.6         Supply Shortage; Inability to Supply.

(a)                    In  the  event  that  PharmaZell  is  unable  or  anticipates  it  will  be  unable  to  supply,  in  whole  or  in  part,  the
quantity of Supplied Material as set forth in any Work Order, PharmaZell shall notify Intercept of such inability upon discovery of the
same  by  PharmaZell,  including  the  underlying  reasons  for  such  inability,  proposed  remedial  measures  and  the  date  such  inability  is
expected to end. In the event that PharmaZell is unable to Manufacture Supplied Material as a result of a shortage of Materials (other
than to the extent such shortage is the result of Intercept’s failure to provide [**]), then PharmaZell hereby agrees and acknowledges that
[**].

(b)          In the event that Intercept is unable to provide [**] to PharmaZell within the project timelines agreed to by the
Parties,  the  Parties  shall  discuss  in  good  faith  allowing  PharmaZell  to  manufacture  [**]  itself  and  for  Intercept  to  purchase  such  [**]
from PharmaZell.

available to Intercept on account of any failure of PharmaZell to Manufacture and supply Supplied Materials hereunder.

(c)          Nothing contained in this Section 2.6 shall limit any legal, equitable or other rights or remedies that may be

2.7         Intercept Materials.

(a)          PharmaZell shall maintain, handle and store the Intercept Materials in accordance with the cGMP, Applicable
Laws and all written instructions as agreed by the Parties. The Intercept Materials shall be stored in a secured area and clearly marked
and  identified  as  property  of  Intercept  clearly  separated  from  other  products  or  materials  by  palette  or  location.  PharmaZell  shall  be
responsible  to  communicate  any  necessary  information  regarding  such  Intercept  Materials  (including  material  safety  data  sheets  and
other  information  provided  to  PharmaZell  relating  to  the  handling  and  safety  of  the  Intercept  Materials)  to  its  employees,  agents  and
representatives engaged in performing the Manufacturing services. PharmaZell shall ensure that Intercept Materials are free and clear of
any liens or encumbrances. PharmaZell shall notify Intercept if at any time it believes Intercept Materials have been damaged, lost or
stolen.

(b)                    PharmaZell  shall  notify  Intercept  when  the  inventories  of  Intercept  Materials  become  insufficient  to
Manufacture  the  API,  as  required  under  this  Agreement.  In  addition,  at  the  end  of  each  calendar  month,  PharmaZell  shall  provide  to
Intercept a stock reconciliation report of the Intercept Materials, which report shall include: (a) the opening stock of Intercept Materials
at the beginning of the month, (b) the receipt of any additional Intercept Materials, (c) the usage of Intercept Materials during the month
(including yield loss), and (d) the stock balance of Intercept Materials.

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under this Agreement and for no other purpose. PharmaZell shall withdraw Intercept Materials from storage on [**].

(c)          PharmaZell shall use the Intercept Materials solely and exclusively to Manufacture the Supplied Materials

(d)          PharmaZell shall at all times take such measures as are required to protect the Intercept Materials from risk of
loss or damage at all stages of the Manufacturing process that are consistent with those measures that PharmaZell utilizes for its own
materials but in no event less than are reasonable and customary in the industry. PharmaZell accepts all risk of loss and full responsibility
for the condition of Intercept Materials which may be damaged, lost or stolen by PharmaZell or its personnel. PharmaZell shall at all
times take such measures as are required to protect the Intercept Materials from risk of loss or damage. Intercept will be responsible for
all transportation costs for such Intercept Materials. Notwithstanding the foregoing, PharmaZell shall be financially responsible for any
loss of such Intercept Materials to the extent such loss results from (a) breach of this Agreement by PharmaZell, (b) negligence or willful
misconduct of PharmaZell, its Affiliates and any permitted subcontractors, in which case PharmaZell shall reimburse Intercept for costs
of such Intercept Materials, plus any shipping costs and out-of-pockets costs incurred by or on behalf of Intercept with respect to such
Intercept Materials.

(e)          PharmaZell shall use its best efforts to obtain standard yields. The standard yields are set forth in Schedule
2.7(e).  The  allowable  annual  yield  variation  from  the  standard  yield  for  the  Intercept  Materials  shall  not  be  more  than  [**].  For
illustration purposes only, an example yield loss calculation is set forth on Schedule 2.7(e). Concurrently with each invoice of Supplied
Materials, PharmaZell shall provide Intercept with a written accounting of the disposition of each yield variation of Intercept Materials.
In the event that the yield variation exceeds the agreed upon allowable yield variation or any losses of Intercept Materials are due to the
negligence  or  willful  misconduct  of  PharmaZell,  Intercept  shall,  at  the  option  of  Intercept,  either  receive  a  reimbursement  from
PharmaZell or reduce Intercept’s payment for the relevant invoice for such Supplied Material in an amount equal to [**]. The Parties
shall  in  good  faith  reevaluate  the  standard  yield  and  the  annual  yield  variation  at  the  beginning  of  each  Calendar  Year  to  account  for
increased efficiencies in the Manufacture of Supplied Material or decreases caused by Required Manufacturing Changes or other agreed
changes to the process.

(f)           In the event that PharmaZell obtains excess yields of the Intercept Materials, PharmaZell will invoice the
excess quantities to Intercept (such excess quantity not to exceed more than [**] of the amount in Intercept’s Work Order), and Intercept
will accept such delivery and invoice.

be [**].

(g)          To the extent Intercept supplies [**] as part of the Intercept Materials, all such [**] provided by Intercept shall

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ARTICLE 3
QUALITY; COMPLIANCE; REGULATORY

3.1         Quality Control.

(a)          Quality Agreement. Intercept and PharmaZell have entered into the Quality Agreement that sets forth the
terms and conditions upon which both Parties will conduct their quality activities in connection with this Agreement. Each Party shall
duly and punctually perform all of its obligations under the Quality Agreement. In the event of any inconsistency between the terms of
this Agreement and the terms of the Quality Agreement, the terms of the Quality Agreement shall control with respect to quality related
matters, and the terms of this Agreement shall control with respect to any other matters.

(b)                    Materials;  Vendor  and  Supplier  Qualification  and  Validation.  PharmaZell  shall  be  responsible  for:  (i)
obtaining  all  starting  Materials  (other  than  Intercept  Materials)  required  to  Manufacture  Supplied  Materials  in  accordance  with  the
Specifications, Applicable Laws and cGMPs and Regulatory Documentation; and (ii) supplying all equipment and personnel necessary
for the performance of the Manufacture and supply of the API to Intercept. The Quality Agreement sets forth additional details regarding
each Party’s obligations regarding Critical Raw Materials (as defined in the Quality Agreement) and in the qualification and validation of
vendors and suppliers retained or contracted in connection with the Manufacture and any other services requested by Intercept.

Supplied Material shall be released by PharmaZell, in each case in accordance with the terms of the Quality Agreement.

(c)                    Analyses.  PharmaZell  shall  be  responsible  for  all  quality  control  analyses  of  Supplied  Materials  and  all

(d)                    Documentation  and  Standard  Operating  Procedures.  PharmaZell  shall  maintain  complete  and  accurate
documentation  of  all  validation  data,  stability  testing  data,  batch  records,  quality  control,  laboratory  testing,  complaint  handling,
deviations, investigations, and corrective and preventative actions and any other data required under cGMPs, Applicable Laws, and other
requirements of any relevant Regulatory Authority in connection with the Manufacture of the Supplied Material. PharmaZell shall make
such  documentation  available  for  inspection  during  any  audit  conducted  by  or  on  behalf  of  Intercept  in  accordance  with  the  Quality
Agreement.  Throughout  the  term  of  this  Agreement,  and  for  so  long  thereafter  as  is  reasonably  necessary,  PharmaZell  shall  strictly
monitor  and  maintain  records  documenting  its  compliance  with  cGMPs  and  any  other  Applicable  Laws,  including  through  the
establishment and implementation of such operating procedures as are reasonably necessary to assure such compliance.

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(e)          Inspection. The Quality Agreement sets forth each Party’s rights and obligations with respect to inspection of
the Supplied Material as well as inspection of the Facilities. Notwithstanding the foregoing and without limiting anything contained in
the Quality Agreement, Intercept shall have the right to audit the Facilities in their entirety and inspect those portions of the Facilities and
the  records  and  information  relating  to  the  Facilities  and  the  Manufacture  of  the  Supplied  Material,  to  determine  and  ensure  that
PharmaZell meets the obligations of the Quality Agreement and is compliant with the Quality Standards. PharmaZell shall permit any
Regulatory  Authority  to  audit  and  inspect  the  Facilities  and  the  Manufacture  of  the  Supplied  Material.  In  connection  with  Intercept’s
determination  of  PharmaZell’s  ability  to  satisfy  the  Quality  Standards  pursuant  to  this  Section  3.1(e),  Intercept  may,  at  Intercept’s
discretion  and  to  the  extent  determined  by  Intercept,  consult  with  PharmaZell  regarding  cGMP  quality,  technical  capability,  and
performance  standards.  If  a  Regulatory  Authority  or  Intercept  identifies  any  observations  in  connection  with  any  audit  or  inspection
under  this  Section  3.1(e)  or  the  Quality  Agreement,  the  Parties  will  discuss  in  good  faith  suitable  approaches  for  correcting  such
observations, and PharmaZell shall have a reasonable time following such consultation with Intercept to make appropriate corrections or
dispute Intercept’s observations (but not dispute a Regulatory Authority’s observations which shall be deemed conclusive). If PharmaZell
disputes  Intercept’s  observations  and  Intercept  and  PharmaZell  are  unable  to  agree  as  to  whether  PharmaZell  meets  the  Quality
Standards, the Parties shall cooperate to have the Facilities and the records and information relating to the Facilities and the Manufacture
of  the  Supplied  Material  inspected  and  audited  by  an  independent  inspection  company  of  recognized  repute  selected  by  Intercept  and
approved by PharmaZell, which approval shall not be unreasonably withheld. The results of such inspection company shall be final and
binding on the Parties on the issue of whether PharmaZell meets the Quality Standards.

(f)           Recalls; Withdrawals. The Quality Agreement sets forth each Party’s rights and obligations with respect to
recalls and withdrawals. If and to the extent such recall or withdrawal is caused by Supplied Material that contains a Deficiency or by
PharmaZell’s negligence or willful misconduct or breach of this Agreement, PharmaZell shall reimburse Intercept for [**]; provided that,
other than with respect to PharmaZell’s gross negligence or willful misconduct, PharmaZell’s liability pursuant to this Section 3.1(f), on
a per claim basis, shall not exceed Fifteen Million United States Dollars ($15,000,000).

accordance with the Quality Agreement.

(g)                    Release.  PharmaZell  shall  perform  Release  Testing  to  ensure  conformance  to  the  Specifications,  in

(h)                    Stability  Testing.  PharmaZell  shall  perform  stability  testing  on  the  API  to  ensure  conformance  to  the

Specifications, in accordance with the Quality Agreement.

3.2         Maintenance of Facility.

exclusively at the Facilities.

(a)                    Except  as  otherwise  approved  in  writing  by  Intercept,  PharmaZell  shall  Manufacture  Supplied  Material

(b)          PharmaZell shall at all times during the Term ensure that any and all licenses, registrations, and Regulatory
Authority approvals required by Applicable Law to be obtained in connection with the Facilities and their operation and equipment used
or to be used in connection with the Manufacture of Supplied Material so as to permit PharmaZell to Manufacture Supplied Material and
supply it to Intercept as contemplated hereunder have been obtained and are in all respects current and in full force and effect.

(c)          PharmaZell shall only use disposal services or sites that have appropriate environmental permits and are in

compliance with Applicable Law.

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3.3         Regulatory Cooperation of PharmaZell. PharmaZell shall cooperate with any reasonable requests for assistance from
Intercept  with  respect  to  obtaining,  maintaining,  and  supporting  any  and  all  Regulatory  Approvals  and  Regulatory  Documentation
required in connection with the sourcing of Supplied Material by Intercept hereunder and the sale of Products, including by:

notice during normal business hours to attend meetings with Regulatory Authorities concerning Supplied Material and Products;

(a)                    at  Intercept’s  cost,  making  PharmaZell  employees,  consultants  and  other  staff  available  upon  reasonable

(b)                    at  PharmaZell’s  own  cost,  disclosing  and  making  available  to  Intercept,  in  whatever  form  Intercept  may
reasonably request, all Manufacturing and quality control data, CMC Data, records, and other information related to Supplied Material,
the Manufacturing process for Supplied Material, and any other services related to Supplied Material as may be reasonably necessary or
desirable  for  Intercept  to  prepare,  file,  obtain,  and  maintain  any  Regulatory  Approval  required  in  connection  with  the  sourcing  of
Supplied Material by Intercept hereunder and the sale of Products, as defined in the Quality Agreement; and

(c)          to the extent that Intercept requests any additional regulatory services from PharmaZell, PharmaZell shall
provide  to  Intercept  a  fee  estimate  for  the  provision  of  such  additional  regulatory  services.  Thereafter,  the  Parties  shall  negotiate  and
agree in advance on the cost and time to provide any such additional regulatory services. Intercept shall not be responsible for the cost or
expense of any amount to the extent that Intercept has not explicitly agreed in writing to pay for such cost or expense.

3.4         Cooperation with Regulatory Authorities and Regulatory Correspondence.

(a)          PharmaZell shall immediately notify Intercept in the event that PharmaZell receives notice from FDA or any
other  relevant  Regulatory  Authority  of  its  intent  to  conduct  any  audit  or  inspection  of  PharmaZell  with  respect  to  the  Facility  or  its
operations, and shall cooperate with the Regulatory Authority in connection with such audit or inspection or related request, including
access to records and documentation related to Manufacturing. Without limiting the foregoing, PharmaZell agrees to immediately notify
Intercept of any correspondence and other documentation received or prepared by either Party in connection with any of the following
events:  (i)  receipt  of  a  Warning  Letter,  FDA  Form  483,  or  other  regulatory  correspondence  from  the  FDA  or  any  other  Regulatory
Authority in connection with the manufacture or design of the API or Product; (ii) any recall of the API or Product; (iii) the mandate,
advice or recommendation from any Regulatory Authority with respect to the withdrawal of any API or Product; and (d) any regulatory
comments from the FDA or any other Regulatory Authority relating to the Manufacture of the Supplied Material.

(b)          As applicable, PharmaZell shall provide copies of any notices or communications to Intercept of any FDA or
other Regulatory Authority inspection, investigation or other inquiry, or other material governmental notice or communication, relating
to the Manufacturing, or Supplied Material. PharmaZell shall consult with Intercept prior to submitting responses to any inquiry posed by
any Regulatory Authority relating to the Manufacturing, Supplied Material or Product. PharmaZell shall not initiate communication with
any Regulatory Authority concerning the Manufacturing, or Supplied Material absent the prior written, express permission of Intercept
concerning any such communications.

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3.5         Compliance with Applicable Law. With respect to the Manufacturing of Supplied Material and PharmaZell’s other
duties  and  obligations  under  this  Agreement,  PharmaZell  shall  strictly  comply  with  (i)  the  Specifications,  (ii)  GMP,  and  all  other
Applicable  Laws,  including  those  relating  to  the  processing,  manufacturing,  packaging,  labeling,  testing,  inspection,  storage,  delivery,
shipment,  or  disposal  of  the  Supplied  Material;  (iii)  the  Quality  Agreement;  and  (iv)  all  Applicable  Laws  concerning  environmental
matters,  public  health,  wages,  hours  and  conditions  of  employment,  subcontractor  selection,  discrimination  and  occupational
health/safety. Without limiting the foregoing, PharmaZell covenants that neither PharmaZell nor any of its permitted subcontractors shall
utilize  child,  or  any  form  of  forced  or  involuntary,  labor  in  the  Manufacture  of  Supplied  Material  under  this  Agreement  or  source
Materials from any supplier that uses child, or any form of forced or involuntary, labor. Upon Intercept’s request, PharmaZell shall certify
in  writing  its  compliance  with  this  Section  3.5  and  shall  provide  to  Intercept  true  and  correct  copies  of  all  permits,  certificates  and
licenses that may be required for its performance under this Agreement and, upon Intercept’s request, permit Intercept to inspect originals
of the same.

3.6         Change Requests.

(a)                    Changes  Requested  by  Intercept.  Intercept  shall  have  the  right  to  request  an  amendment,  change  or
supplement to any of the following upon written notice to PharmaZell, and except as may be prohibited by Applicable Law, PharmaZell
shall use its commercially reasonable efforts to promptly implement such change: (a) the Specifications, (b) the Materials, (c) the source
of Materials, (d) the specifications for Materials, (e) the equipment used in Manufacture, (f) the test methods used in connection with the
Manufacturing  of  Supplied  Material  and  Materials,  (g)  the  process  for  Manufacturing  Supplied  Material,  or  (h)  any  test  methods  to
Manufacture or release Supplied Material. PharmaZell shall ensure that any change in any of the foregoing shall, in each case, comply
with cGMPs and all Applicable Laws. PharmaZell and Intercept will jointly discuss the cost resulting from such changes.

(b)          Required Manufacturing Changes. Each Party shall give the other Party reasonable written notice prior to any
changes to the Specifications, process of Manufacturing, or other change, as applicable, with respect to the Supplied Materials, in each
case that are required by cGMPs or Applicable Laws or a Regulatory Authority (collectively, “Required  Manufacturing  Changes”).
PharmaZell shall use commercially reasonable efforts to promptly implement such Required Manufacturing Changes. PharmaZell shall
ensure  that  any  change  in  any  of  the  foregoing  shall,  in  each  case,  comply  with  cGMPs  and  all  Applicable  Laws.  PharmaZell  and
Intercept will jointly discuss the cost resulting from such changes.

3.7                  General Cooperation.  PharmaZell  shall  cooperate  with  any  reasonable  requests  for  assistance  from  Intercept  and
collaborate  with  Intercept  with  respect  to  any  responses  by  Intercept  to  any  Regulatory  Authority  and  requests  for  information  from
Regulatory Authorities, pharmacovigilance and recall matters, and in accommodating Intercept’s needs for Supplied Materials, including
accepting changes in forecasting and Work Orders.

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4.1         Price.

ARTICLE 4
FINANCIALS

follows:

(a)          Subject to Section 4.4, the purchase price (the “Purchase Price”) for Supplied Material shall be determined as

Amount of Supplied Material
Ordered for Delivery in a
Calendar Year
[**]
[**]
[**]
[**]

Price

[**]
[**]
[**]
[**]

(b)          For purposes of determining the Purchase Price applicable to a given quantity of Supplied Material that is
ordered for delivery for a given Calendar Year, any quantity of Supplied Material that has been ordered by Intercept for delivery in a
given Calendar Year shall be deemed ordered for delivery for such Calendar Year even if such quantity is ordered or Manufactured in an
earlier Calendar Year. If Intercept places multiple orders for delivery in the same Calendar Year, such that the total amount of Supplied
Material ordered for delivery in such Calendar Year in the aggregate is in a higher tier than a previously placed order, the Parties shall
reconcile the total amount ordered for delivery in such Calendar Year and recalculate the Purchase Price and PharmaZell shall pay to
Intercept the difference or, to the extent the final invoice for such Calendar Year has not yet been paid, Intercept may reduce the amount
of such invoice accordingly. For example, and by way of illustration purposes only, if Intercept places an order for [**].

4.2         Invoice and Payment. PharmaZell shall invoice Intercept for the Manufacture of Supplied Material as follows:

(a)          PharmaZell shall be entitled to invoice Intercept for a certain percentage of the total Purchase Price calculated
in  accordance  with  Section  4.1(a)  in  accordance  with  the  Work  Order  for  such  Supplied  Material  prior  to  delivery  of  the  Supplied
Material upon achievement of certain steps of the Manufacturing process as follows:

Milestone
[**]
[**]
[**]
[**]
[**]
[**]
[**]

Step of Manufacturing
Process

Percentage of total
Purchase Price

[**] 
[**] 
[**] 
[**] 
[**] 
[**] 
[**] 

[**]
[**]
[**]
[**]
[**]
[**]
[**]

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(b)          Prior to PharmaZell issuing an invoice to Intercept pursuant to Section 4.2(a), PharmaZell shall provide to
Intercept the batch documentation and the testing and analytical data, if applicable, for such step of the Manufacturing to demonstrate to
Intercept  that  PharmaZell  has  successfully  completed  such  step  of  the  Manufacturing.  Upon  Intercept’s  acceptance  of  the  batch
documentation and the testing and analytical data, if applicable, but no later than [**] days after PharmaZell has provided such batch
documentation, PharmaZell shall invoice Intercept for the percentage of the total Purchase Price for such step of the Manufacturing in
accordance with Section 4.2(a) and payment shall be due [**] days after receipt of such invoice by Intercept.

(c)          PharmaZell promptly shall invoice Intercept for the remaining amount of the total Purchase Price calculated
pursuant  to  Section  4.1  for  the  quantities  of  API  actually  delivered  (subject  to  Section  2.7(f))  to  Intercept;  provided  that  if  the  total
quantity of API actually delivered is less than [**] of the total quantity ordered for delivery, PharmaZell shall reimburse Intercept for the
amounts overpaid pursuant to Section 4.2(a) and the amount actually delivered. Payment for the remaining amount of the total Purchase
Price for the quantity of Supplied Material actually delivered shall be due [**] days after receipt by Intercept of the invoice and receipt of
corresponding  Supplied  Material  with  respect  thereto  (which  shall  be  sent  in  electronic  form  contemporaneously  with  such  delivery);
provided that if Intercept rejects such Supplied Material, then payment shall be due within [**] days after receipt by Intercept of notice
from  the  Testing  Laboratory  that  the  invoiced  Supplied  Material  does  not  contain  a  Deficiency  or  receipt  by  Intercept  of  replacement
Supplied Material, as the case may be. If the Supplied Material contains a Deficiency and Intercept does not order replacement Supplied
Material, PharmaZell shall promptly reimburse all amounts previously paid by Intercept for such Supplied Material pursuant to Section
4.2(b).

(d)                    If  Intercept  disputes  any  portion  of  an  invoice,  it  shall  pay  the  undisputed  portion  and  shall  provide
PharmaZell with written notice of the disputed portion and its reasons therefor, and Intercept shall not be obligated to pay such disputed
portion.  The  Parties  shall  use  good  faith  efforts  to  resolve  any  such  disputes  promptly.  In  the  event  of  any  inconsistency  between  an
invoice and this Agreement, the terms of this Agreement shall control. Payment of invoices shall be made by wire transfer to an account
designated in writing by PharmaZell.

4.3         Currency. PharmaZell will invoice Intercept in [**] and Intercept will pay in [**]. The exchange rate of [**] to [**] at
the date of the last signature to this Agreement will be used as Reference Exchange Rate. Should at any time during the Agreement for a
period longer than [**] months the then current exchange rate of [**] to [**] deviates more than [**] from the Reference Exchange Rate,
both Parties will discuss in good faith impact on Prices and cost and adjust Price as agreed by the Parties in writing.

4.4         Adjustment of Purchase Price.

“Adjustment Date”). Effective on [**], the Purchase Price for such Supplied Material shall be adjusted by [**].

(a)                    The  Purchase  Prices  set  forth  in  Section  4.1  for  Supplied  Material  shall  remain  fixed  until  [**]  (the

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(b)          If at any time market conditions (raw material costs e.g.) result in PharmaZell’s cost of components for the
API or manufacturing process being materially greater [**] than normal forecasted increases, then PharmaZell shall be entitled to request
an adjustment to the pricing of the Supplied Material to compensate for such increased cost. The Parties shall negotiate in good faith such
increase.

(c)                    If  at  any  time  market  conditions  result  in  PharmaZell’s  cost  of  components  for  the  Supplied  Material  or
manufacturing process being materially less [**] than normal, then Intercept shall be notified and an adjustment to the pricing will be
given to compensate for such decreased cost.

(d)          The Parties agree to make reasonable efforts to improve the productivity, efficiency and quality of the process
under which the Supplied Material is Manufactured. Any investment and/or cost savings as a result of such improvement shall be shared
equitably between the Parties.

4.5         Audit; Late Payments.

(a)          Intercept shall have the right to have an independent accounting firm of internationally recognized standing,
and reasonably acceptable to PharmaZell, provided with access by PharmaZell during normal business hours, and upon reasonable prior
written  notice,  to  examine  only  those  records  of  PharmaZell  (and  its  Affiliates)  as  may  be  reasonably  necessary  to  determine,  with
respect  to  any  Calendar  Year  ending  not  more  than  [**]  prior  to  Intercept’s  request,  the  correctness  of  any  statement  submitted  by
PharmaZell under this Agreement. Such examinations may not (i) be conducted more than once in any [**] period (unless a previous
audit during such [**] period revealed an incorrect statement submitted by PharmaZell in respect of such period or PharmaZell restates
or revises its books and records for such period) or (ii) be repeated for any Calendar Year. Results of such audit shall (i) be (A) limited to
information relating to the supply of Supplied Material hereunder and use of the Intercept Materials, (B) made available to both Parties in
writing, and (C) subject to ARTICLE 7 and (ii) not reveal any specific information of PharmaZell to Intercept other than (A) whether
statements submitted by PharmaZell under this Agreement are true and correct and (B) the amount of any excess payment reimbursable
to Intercept. The cost of any such examination shall be borne by Intercept unless the examination reveals a variance of more than [**]
from  the  amounts  reflected  on  PharmaZell’s  statements,  in  which  case  PharmaZell  shall  bear  the  cost  of  the  audit.  Unless  disputed
pursuant to Section 4.5(c), if such audit concludes that excess payments were made by Intercept during such period, PharmaZell shall
reimburse such amounts, with interest from the date originally due as provided in Section 4.5(d), within [**] days after the date on which
such auditor’s written report is delivered to the Parties.

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(b)          Solely for the purposes of ensuring Intercept’s compliance with Section 2.2(b), PharmaZell shall have the
right  to  have  an  independent  accounting  firm  of  internationally  recognized  standing,  approved  by  Intercept,  during  normal  business
hours, and upon reasonable prior written notice which notice shall be at least [**] days prior to the audit, to examine only those records
of Intercept (and its Affiliates) as may be necessary to determine whether Intercept has met its Minimum Percentage Requirement, with
respect to any Calendar Year ending not more than [**] prior to PharmaZell’s request. Such examinations may not be conducted more
than  once  in  any  [**]  period.  The  results  communicated  to  Pharmazell  regarding  any  such  audit  shall  be  limited  solely  to  whether
Intercept  ordered  the  Minimum  Percentage  Requirement  for  such  Calendar  Year  and  any  deviations  from  the  Minimum  Percentage
Requirement.  No  other  information  may  be  included  in  the  audit  results  and  the  audit  results  must  be  concurrently  communicated  to
Intercept in writing. The cost of any such examination shall be borne by PharmaZell. Unless disputed pursuant to Section 4.5(c), if such
audit  concludes  that  Intercept  did  not  order  the  Minimum  Percentage  Requirement  for  such  Calendar  Year,  Intercept  shall  order  an
additional amount of Supplied Material in a subsequent calendar year equal to the difference between the amount of Supplied Material
Intercept actually ordered from PharmaZell in such Calendar Year and the amount Intercept would have ordered had Intercept actually
ordered the Minimum Percentage Requirement for such Calendar Year.

(c)          In the event of a dispute of any examination conducted under Section 4.5, PharmaZell and Intercept shall
work in good faith to resolve the disagreement. If the Parties are unable to reach a mutually acceptable resolution of any such dispute
within [**] days, the dispute shall be resolved in accordance with Section 10.7.

(d)          If any undisputed payment due to a Party under this Agreement is not paid when due, then the owing Party
shall pay interest thereon (before and after any judgment) at an annual rate (but with interest accruing on a daily basis) equal to the lesser
of  [**],  and  [**].  Interest  payable  under  this  Section  4.5(d)  shall  run  from  the  date  upon  which  payment  of  the  relevant  undisputed
principal sum became due through the date of payment thereof in full together with such interest.

ARTICLE 5
INTELLECTUAL PROPERTY

5.1         Ownership of Inventions.

(a)          Intercept shall own all right, title and interest in and to (i) the Specifications and the Intercept Information, (ii)
any  and  all  Specified  Inventions,  (iii)  the  API  and  the  API  Precursor,  and  (iv)  any  and  all  work  outputs  and  reports  prepared  by
PharmaZell  (together,  “Intercept  Intellectual  Property”).  PharmaZell  shall,  and  shall  cause  its  Affiliates  to,  promptly  disclose  in
writing to Intercept the discovery, development, making, conception or reduction to practice of any Specified Invention and does hereby,
and shall cause its Affiliates, employees, agents, subcontractors to, assign to Intercept any and all right, title or interest PharmaZell or its
Affiliates  may  have  in  or  to  any  Specified  Invention.  Intercept  shall,  and  does  hereby,  grant  to  PharmaZell  and  its  Affiliates  a  non-
exclusive, royalty-free license to use the Specifications, Intercept Information, Specified Inventions, and Specified Invention Patents for
the sole purpose of performing PharmaZell’s obligations hereunder. The Specified Inventions and the work outputs and reports shall be
considered Intercept Information.

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(b)          PharmaZell shall keep complete, accurate and dated records of the results of the services performed under this
Agreement  and  all  Specified  Inventions  and  will  promptly  and  fully  disclose  to  Intercept  such  results  and  Specified  Inventions.  Such
records shall also identify the names of PharmaZell’s employees, officers or Affiliates who performed the work. Intercept may discuss, in
person or otherwise, the services and the results thereof from time to time with PharmaZell and such employees. PharmaZell agrees that
it shall not publish or present any information related to the Intercept Information, the Product, API or the results thereof, any Specified
Inventions or any other Intercept Intellectual Property without the prior written consent of Intercept unless PharmaZell is legally obliged
to do so. PharmaZell must identify and obtain Intercept’s approval prior to inclusion of any PharmaZell technology into any Supplied
Material or other deliverable hereunder.

(c)                    PharmaZell  shall  own  all  right,  title  and  interest  in  and  to  any  and  all  Other  PharmaZell  Inventions.
PharmaZell  shall,  and  shall  cause  its  Affiliates  to,  promptly  disclose  in  writing  to  Intercept  the  discovery,  development,  making,
conception  or  reduction  to  practice  of  any  Other  PharmaZell  Invention.  PharmaZell  shall,  and  does  hereby,  grant  to  Intercept  a  non-
exclusive, royalty-free, irrevocable and transferable license to Other PharmaZell Inventions and Other PharmaZell Invention Patents and,
to  any  PharmaZell  technology  to  the  extent  it  is  incorporated  into  or  otherwise  necessary  to  Manufacture  or  use  API  (including  any
Intermediary incorporated therein), with the right to sublicense through multiple tiers, to Exploit API and Products (and any Intermediary
incorporated therein) in all fields of use in all countries worldwide.

(d)          PharmaZell and Intercept shall jointly own all right, title and interest in and to any and all Joint Inventions.
Each of PharmaZell and Intercept shall, and shall cause its respective Affiliates to, promptly disclose in writing to the other Party the
discovery,  development,  making,  conception  or  reduction  to  practice  of  any  Joint  Invention.  For  those  countries  worldwide  where  a
specific  license  is  required  to  be  granted  by  a  Joint  Invention  owner  to  the  other  Joint  Invention  owner  in  order  for  the  other  Joint
Invention  owner  to  practice  such  Joint  Inventions  in  such  country,  (i)  PharmaZell  shall,  and  does  hereby,  grant  to  Intercept  a  non-
exclusive, royalty-free, irrevocable, transferable license, with the right to sublicense through multiple tiers, to PharmaZell's interest in all
Joint  Inventions  and  Joint  Invention  Patents  in  all  fields  of  use  and  (ii)  Intercept  shall,  and  does  hereby,  grant  to  PharmaZell  a  non-
exclusive,  royalty-free,  irrevocable  license,  with  the  right  to  sublicense  through  multiple  tiers,  to  Intercept  's  interest  in  all  Joint
Inventions and Joint Invention Patents in all fields of use.

Information solely for purposes of performing its obligations hereunder.

(e)          Without limiting the provisions of this Section 5.1, PharmaZell shall use the Specifications and Intercept

(f)                      Upon  the  request  and  at  the  expense  of  Intercept,  PharmaZell  shall  execute  and  deliver  any  and  all
instruments and documents and take such other acts as may be necessary or desirable to document the assignment and transfer described
in Section 5.1(a) or to enable Intercept to secure its rights in the Specified Invention and Specified Invention Patents relating thereto in
any and all jurisdictions, or to apply for, prosecute and enforce Specified Invention Patents, or to obtain any extension, validation, re-
issue,  continuance  or  renewal  of  any  such  Specified  Invention  Patents.  Without  limiting  the  foregoing,  PharmaZell  shall  disclose  to
Intercept  all  pertinent  information  and  data  with  respect  thereto  and  shall  execute  all  applications,  specifications,  oaths  and  all  other
instruments which Intercept deems necessary in order to apply for and obtain such rights and in order to assign and convey to Intercept
the sole and exclusive right, title and interest in and to such Specified Invention Patents relating thereto. If Intercept is unable for any
other reason to secure PharmaZell’s signature to apply for or to pursue any application for any United States or foreign patent, trademark,
copyright or other registration covering Inventions assigned to Intercept hereunder, then PharmaZell hereby irrevocably designates and
appoints Intercept and its duly authorized officers and agents as PharmaZell’s agent and attorney in fact, to act for and in PharmaZell’s
behalf  and  instead  to  execute  and  file  any  such  applications  and  to  do  all  other  lawfully  permitted  acts  to  further  the  prosecution  and
issuance  of  letters  patent  or  trademark,  copyright  or  other  registrations  thereon  with  the  same  legal  force  and  effect  as  if  executed  by
PharmaZell.

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(g)                    Inventorship  Acts.  To  the  extent  applicable,  the  Parties  understand  that  Inventions  that  are  conceived,
developed,  generated  or  reduced  to  practice  under  this  Agreement  may  be  subject  to  the  German  Act  on  Employee  Inventions  (the
German  “Gesetz  über  Arbeitnehmererfindungen”).  The  provisions  of  such  Gesetz  über  Arbeitnehmererfindungen  are,  inter  alia,
designed to protect the rights of employees to so called employee inventions (the “Employee Inventions”); the provisions of the Gesetz
über Arbeitnehmererfindungen constitute inalienable rights which may not be changed by contractual arrangements to the detriment of
the  employees.  To  the  extent  that  Inventions  relate  to  Employee  Inventions  under  the  German  Gesetz  über  Arbeitnehmererfindungen
made  by  employees  of  a  Party  or  its  Affiliates,  such  Party  undertakes  to  claim  the  rights  in  and  to  such  Employee  Inventions  under
Section  5ss.  of  the  Gesetz  über  Arbeitnehmererfindungen.  To  the  extent  that  such  Party  acquires  rights  to  Employee  Inventions  in
accordance with the principles stated in this Section 5.1(g), the further provisions of this 5.1 shall apply to such Inventions. The Party
subject to the Gesetz über Arbeitnehmererfindungen shall be solely responsible for any payments to its employees and such Party will
take all actions necessary to obtain the rights to use any such Inventions for the other Party. In addition, PharmaZell shall comply with all
other inventorship laws of a country in which any portion of a Supplied Material is Manufactured.

5.2         Patent Prosecution.

(a)          Specified Invention Patents.

(i)                    Intercept  shall  have  sole  discretion  and  responsibility  to  prepare,  file,  prosecute  and  maintain  all
patent applications and patents covering Specified Inventions (the “Specified Invention Patents”) and shall be responsible for related
interference and opposition proceedings. PharmaZell shall have no right to prepare, file, prosecute or maintain any Specified Invention
Patents.

(ii)         Costs and expenses of filing, prosecuting and maintaining (including any costs and expenses of patent
interference,  opposition,  reissue,  re-examination,  and  post-grant  procedure  proceedings)  Specified  Invention  Patents  shall  be  borne  by
Intercept.

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(b)          Other PharmaZell Invention Patents.

(i)          PharmaZell shall have the first right, but not the obligation, to prepare, file, prosecute and maintain
all  patent  applications  and  patents  covering  Other  PharmaZell  Inventions  (the  “Other  PharmaZell  Invention  Patents”)  and  shall  be
responsible  for  related  interference  and  opposition  proceedings;  provided,  however,  that  if  PharmaZell  plans  to  abandon  any  Other
PharmaZell Invention Patent, PharmaZell shall notify Intercept in writing at least [**] days in advance of the due date of any payment or
other  administrative  action  that  is  required  to  maintain  such  Other  PharmaZell  Invention  Patent  (i.e.,  an  administrative  action  that
involves  routine  and  customary  filings,  it  being  understood  that  interference,  opposition,  reissue,  re-examination,  and  post-grant
procedure proceedings, prosecution or defense of infringement actions, and the like, shall not be considered administrative actions), and
Intercept may elect, upon written notice within such [**]-day period to PharmaZell, to make such payment or take such administrative
action  on  behalf  of  PharmaZell.  Except  as  expressly  permitted  in  this  Section  5.2(b)(i),  Intercept  shall  have  no  right  to  prepare,  file,
prosecute or maintain any Other PharmaZell Invention Patents.

(ii)         If PharmaZell does not wish to file, prosecute or maintain any Other PharmaZell Invention Patent or
maintain  or  defend  any  Other  PharmaZell  Invention  Patent  in  a  particular  country,  it  shall  notify  Intercept  in  writing  and,  if  Intercept
elects to maintain such Other PharmaZell Invention Patent as contemplated by Section 5.2(b)(i), PharmaZell shall, and shall cause its
Affiliates, as applicable, to (A) reasonably cooperate with Intercept in this regard and, (B) upon Intercept’s request, promptly release or
assign to Intercept, without compensation, all right, title and interest in and to such Other PharmaZell Invention Patent in such country. In
the event of such assignment, Intercept hereby grants to PharmaZell a non-exclusive, royalty-free, irrevocable license, with the right to
sublicense through multiple tiers, under the relevant Other PharmaZell Invention Patent in all fields of use in the relevant country.

(iii)                Costs  and  expenses  of  filing,  prosecuting  and  maintaining  (including  any  costs  and  expenses  of
patent  interference,  opposition,  reissue,  re-examination,  and  post-grant  procedure  proceedings)  Other  PharmaZell  Invention  Patents  as
contemplated by this Section 5.2(b) shall be borne by the Party controlling such filing, prosecution and maintenance.

(c)          Joint Invention Patents.

(i)          Intercept shall have the first right, but not the obligation, to prepare, file, prosecute and maintain all
patent  applications  and  patents  covering  Joint  Inventions  (the  “Joint  Invention  Patents”)  and  shall  be  responsible  for  related
interference and opposition proceedings; provided, however, that if Intercept plans to abandon any Joint Invention Patent, Intercept shall
notify PharmaZell in writing at least [**] days in advance of the due date of any payment or other administrative action that is required to
maintain such Joint Invention Patent (i.e., an administrative action that involves routine and customary filings, it being understood that
interference, opposition, reissue, re-examination, and post-grant procedure proceedings, prosecution or defense of infringement actions,
and the like, shall not be considered administrative actions), and PharmaZell may elect, upon written notice within such [**]-day period
to  Intercept,  to  make  such  payment  or  take  such  administrative  action  on  behalf  of  Intercept.  Except  as  expressly  permitted  in  this
Section 5.2(c)(i), PharmaZell shall have no right to prepare, file, prosecute or maintain any Joint Invention Patents.

(ii)         If Intercept does not wish to file, prosecute or maintain any Joint Invention Patent or maintain or
defend any such Joint Invention Patent in a particular country, it shall notify PharmaZell in writing and, if PharmaZell elects to maintain
such  Joint  Invention  Patent  as  contemplated  by  Section  5.2(c)(i),  Intercept  shall,  and  shall  cause  its  Affiliates,  as  applicable,  to
reasonably cooperate with PharmaZell in this regard.

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(iii)                Costs  and  expenses  of  filing,  prosecuting  and  maintaining  (including  any  costs  and  expenses  of
patent interference, opposition, reissue, re-examination, and post-grant procedure proceedings) Joint Invention Patents as contemplated
by this Section 5.2(c) shall be borne by the Party controlling such filing, prosecution and maintenance.

time to time in connection with its activities set forth in this Section 5.2.

(d)          Each Party shall assist and cooperate with the other Party as such other Party may reasonably request from

(i)          Each Party shall keep the other Party currently informed of all steps to be taken in the preparation and
prosecution of all applications filed by it according to Sections 5.2(b) and 5.2(c) and shall furnish such other Party with copies of such
applications for patents, amendments thereto and other related correspondence to and from patent offices, and, to the extent reasonably
practicable, permit such other Party an opportunity to offer its comments thereon before making a submission to a patent office which
could  materially  affect  the  scope  or  validity  of  the  patent  coverage  that  may  result.  Such  other  Party  shall  offer  its  comments,  if  any,
promptly.

5.3         Enforcement of Patents.

(a)          If any Specified Invention Patent, Other PharmaZell Invention Patent, or Joint Invention Patent is allegedly or
actually infringed by any Person, the Party first having knowledge of such infringement shall promptly notify the other in writing. The
notice shall set forth the facts of that infringement in reasonable detail.

(b)          As between the Parties, Intercept shall have the sole and exclusive right, but not the obligation, to prosecute
any infringement described in Section 5.3(a). To the extent any such action relates to an Other PharmaZell Invention Patent or a Joint
Invention Patent, PharmaZell shall have the right, at its own expense, to be represented in any such action by counsel of its own choice.

(c)          PharmaZell shall cooperate fully, including furnishing of a power of attorney, being joined as a party plaintiff
or indispensable party in such action, providing access to relevant documents and other evidence, and making its employees available at
reasonable business hours in connection with any enforcement action that may be brought by Intercept under this Section 5.3.

(d)          Any costs and expenses relating to any enforcement action commenced by Intercept pursuant to this Section
5.3 shall be borne by Intercept and any damages or other amounts collected in any such enforcement action shall be retained by Intercept.

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5.4         Third Party Litigation.

(a)          If any Person institutes against PharmaZell any action that alleges that the Manufacture of Supplied Material
hereunder in accordance with the terms hereof infringes the intellectual property rights held by such Person, then, as between PharmaZell
and Intercept, Intercept shall have the first right, but not the obligation, to contest, and assume direction and control of the defense of,
such action, including the right to settle such action; provided that, prior to any such settlement, PharmaZell provides its written consent
(such consent not to be unreasonably withheld, conditioned or delayed). If Intercept determines not to defend against such action, then
PharmaZell shall, at its sole cost and expense, have the right but not the obligation to control the defense of such action except to the
extent it relates to a Specified Invention Patent; provided that, if an Other PharmaZell Invention Patent or Joint Invention Patent is at
issue in the action and is the only patent protecting a Product, then PharmaZell shall in any event consult with Intercept with respect to
any such action and shall obtain Intercept's written consent prior to taking any steps in respect of such action. Intercept shall have the
right, at its own expense, to be represented in any such action by counsel of its own choice.

(b)          Any costs and expenses relating to any defense undertaken pursuant to this Section 5.4 shall be borne by the
Party controlling the defense. Any damages or other amounts recovered shall be first allocated to reimburse the Parties for their costs and
expenses in making such recovery (which amounts shall be allocated pro rata if insufficient to cover the totality of such expenses). Any
remainder after such reimbursement is made shall be retained by the Party that has exercised its right to control the defense of the action.

(c)          In the event that a Party entitled to defend an infringement action does so in accordance with this Section 5.4,
the  other  Party  shall  cooperate  fully,  including  providing  access  to  relevant  documents  and  other  evidence  and  making  its  employees
available at reasonable business hours. If a Party pursues the defense of such an infringement action, it shall consider in good faith any
comments from the other Party and shall keep the other Party reasonably informed of any steps taken to remedy such infringement.

5.5         Third Party Licenses. If, in the absence of a license from a Person, the Manufacture of API or API Precursor hereunder
in accordance with the terms hereof infringes or misappropriates any patent or any intellectual property right of such Person, such that
PharmaZell or any of its Affiliates cannot Manufacture the API or API Precursor without infringing the patent or intellectual property
rights of such Person, then Intercept shall have the sole and exclusive right to take the lead in negotiating the terms of any such license.
The Parties shall negotiate in good faith an appropriate allocation of any royalties or other payments to be made pursuant to any such
license so as to reflect the economic interests of the Parties under this Agreement with respect to the Product.

5.6         United States Law. The determination of whether Inventions are conceived, discovered, developed or otherwise made
by a Party for the purpose of allocating proprietary rights (including patent, copyright or other intellectual property rights) therein, shall,
for purposes of this Agreement, be made in accordance with Applicable Law in the United States. In the event that United States law
does  not  apply  to  the  creation,  conception,  discovery,  development  or  making  of  any  Invention  hereunder,  each  Party  shall,  and  does
hereby, assign, and shall cause its Affiliates to so assign, to the other Party, without additional compensation, such right, title and interest
in  and  to  any  Inventions,  as  well  as  any  intellectual  property  rights  with  respect  thereto,  as  necessary  to  fully  effect  ownership  as
contemplated by Section 5.1 and the preceding sentence of this Section 5.6.

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ARTICLE 6
REPRESENTATIONS AND WARRANTIES; COVENANTS

6.1         Representations and Warranties of Each Party. Each Party hereby represents and warrants to the other Party as of the

Effective Date, and covenants with the other Party, as follows:

(a)          Such Party (i) is duly formed and in good standing under the laws of the jurisdiction of its formation, (ii) has
the  power  and  authority  and  the  legal  right  to  enter  into  this  Agreement  and  perform  its  obligations  hereunder,  and  (iii)  has  taken  all
necessary action on its part required to authorize the execution and delivery of this Agreement and the performance of its obligations
hereunder.  This  Agreement  has  been  duly  executed  and  delivered  on  behalf  of  such  Party  and  constitutes  a  legal,  valid  and  binding
obligation  of  such  Party  and  is  enforceable  against  it  in  accordance  with  its  terms,  subject  to  the  effects  of  bankruptcy,  insolvency  or
other similar laws of general application affecting the enforcement of creditor rights and judicial principles affecting the availability of
specific performance and general principles of equity, whether enforceability is considered in a proceeding at law or equity;

(b)          All necessary consents, approvals and authorizations of all Regulatory Authorities and other Persons required
to  be  obtained  by  such  Party  in  connection  with  the  execution  and  delivery  of  this  Agreement  and  the  performance  of  its  obligations
hereunder have been obtained; and

(c)          The execution and delivery of this Agreement and the performance of such Party’s obligations hereunder
(i)  do  not  and  will  not  conflict  with  or  violate  any  requirement  of  Applicable  Law  or  any  provision  of  the  articles  of  incorporation,
bylaws,  limited  partnership  agreement  or  other  similar  documents  of  such  Party  and  (ii)  do  not  and  will  not  conflict  with,  violate,  or
breach, or constitute a default or require any consent under, any contractual obligation or court or administrative order by which such
Party is bound.

6.2         Additional Representations, Warranties and Covenants of PharmaZell. PharmaZell hereby represents and warrants to

Intercept as of the Effective Date, and covenants to Intercept, as follows:

(a)                    PharmaZell  has  executed  agreements  with  all  Affiliates,  employees,  agents  subcontractors  and  any  other
representative of PharmaZell performing services for PharmaZell in connection with the Manufacture and supply of Supplied Materials
to Intercept, or its designee (each, a “Representative”) requiring such Representative to assign all right, title and interest in and to any
intellectual property conceived, discovered, developed or otherwise made by such Representative to PharmaZell;

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(b)                    In  connection  with  each  delivery,  and  as  of  the  date  of  delivery,  of  Supplied  Materials  to  Intercept  or  its
designee:  (i)  such  Supplied  Material  has  been  Manufactured  in  compliance  with  the  Specifications  and  is  in  conformity  with  the
Specifications,  the  Certificate  of  Analysis  and  the  Certificate  of  Conformance  therefor  provided  pursuant  to  Section  2.3(b);  (ii)  such
Supplied Material has been Manufactured, stored, disposed of and handled in conformance with GMP, all other Applicable Laws, the
Regulatory Documentation and Regulatory Approvals, this Agreement and the Quality Agreement; (iii) title to such Supplied Material
will  pass  to  Intercept  free  and  clear  of  any  security  interest,  lien  or  other  encumbrance;  (iv)  the  Facilities  are  in  compliance  with  all
Applicable  Law  at  the  time  of  such  Manufacture  (including  applicable  inspection  requirements  of  FDA  and  other  Regulatory
Authorities);  (v)  the  retest  date  of  such  Supplied  Material  meets  the  retest  set  forth  in  the  Specifications  or  otherwise  determined  in
accordance with Applicable Law after the date of delivery thereof for such Supplied Material; and (vi) such Supplied Material has not
been  adulterated  or  misbranded  within  the  meaning  of  the  FFDCA  or  other  Applicable  Law,  or  is  an  article  that  may  not,  under  the
FFDCA or other Applicable Law, be introduced into interstate commerce (collectively, the “Supplied Material Warranty”);

(c)          neither PharmaZell nor any of its Affiliates, nor any Third Party engaged by PharmaZell has ever been, are
currently,  nor  during  the  performance  of  any  services  hereunder,  shall  become:  (i)  disqualified  or  debarred  by  the  FDA  or  other
Regulatory  Authorities  for  any  purpose  pursuant  to  Applicable  Laws  (including  United  States  law,  including  the  statutory  debarment
provisions at 21 U.S.C. § 335a(a) or (b)) or is under consideration or investigation to be disqualified or debarred, or has been convicted
of, or is currently charged with, a felony for conduct relating to the development, approval, regulation or handing of any drug product
under any Applicable Law; (ii) charged or convicted for conduct relating to the development or approval of, or otherwise relating to the
regulation  of,  any  drug  product  under  any  Applicable  Laws;  (iii)  excluded  or,  to  the  best  of  the  knowledge  of  PharmaZell  after  due
inquiry, threatened with exclusion under state or federal laws, including under 42 U.S.C. § 1320a-7 or relevant regulations in 42 C.F.R.
Part  1001,  or  assessed  or,  to  the  best  of  the  knowledge  of  PharmaZell  after  due  inquiry,  threatened  with  assessment  of  civil  money
penalties  pursuant  to  42  U.S.C.  Part  1003;  (iv)  ineligible  for  contract  with  the  federal  government,  including  due  to  disbarment,
disqualification, or conviction of a felony related to conduct relating to the development, approval, regulation or handing of any drug
product under any Applicable Law; or (v) subject to similar actions by any state, local, or foreign governmental authority (collectively
“Disqualification”).  PharmaZell  agrees  to  notify  Intercept  immediately,  in  the  event  that  PharmaZell  or  any  of  its  officers,  directors,
employees, agents, or parties under contract to perform and work under this Agreement, (i) becomes subject to Disqualification, or (ii)
receives or becomes aware of an action, notice of action, inquiry, or investigation with relating to or that could result in Disqualification
during the Term. In the event that PharmaZell receives any notice of actions set forth in this Section 6.2(c), without limiting any other
rights or remedies of Intercept, Intercept shall have the right to terminate this Agreement immediately pursuant to the provisions of this
Agreement. Any termination by Intercept pursuant to this Section 6.2(c) shall be deemed to be a termination by Intercept for material
breach of this Agreement by PharmaZell;

(d)          its retention as a contractor by Intercept and its Manufacture of Supplied Material do not, and shall not, breach
any  agreement  that  obligates  PharmaZell  to  keep  in  confidence  any  trade  secrets  or  confidential  information  of  any  third  party  or  to
refrain from competing, directly or indirectly, with the business of any other party;

(e)                    the  Manufacture  and  supply  of  the  Supplied  Material  shall  be  performed  with  requisite  care,  skill  and
diligence, in accordance with this Agreement, Applicable Laws and industry standards, and by individuals who are appropriately trained
and qualified; and

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(f)           the Manufacturing services provided under this Agreement will not infringe the intellectual property rights of
any  third  party,  and  PharmaZell  will  promptly  notify  Intercept  in  writing  should  it  become  aware  of  any  claims  asserting  such
infringement.

6.3         Disclaimer of Other Warranties. EXCEPT AS EXPRESSLY SET FORTH IN THIS AGREEMENT, NEITHER PARTY
MAKES  ANY  REPRESENTATIONS  AND  EXTEND  NO  WARRANTIES  OF  ANY  KIND,  EITHER  EXPRESS  OR  IMPLIED,
INCLUDING ANY WARRANTY OF FITNESS FOR A PARTICULAR PURPOSE OR WARRANTY OF MERCHANTABILITY.

ARTICLE 7
CONFIDENTIALITY

7.1         Confidential Information. Subject to the provisions of Sections 7.2 and 7.3, at all times during the Term and for [**]
following  the  expiration  or  termination  of  this  Agreement,  the  Receiving  Party  (a)  shall  keep  completely  confidential  and  shall  not
publish  or  otherwise  disclose  any  Confidential  Information  furnished  to  it  by  the  Disclosing  Party,  except  to  those  of  the  Receiving
Party’s employees, Affiliates, or consultants who have a need to know such information to perform such Party’s obligations hereunder
(and who shall be advised of the Receiving Party’s obligations hereunder and who are bound by confidentiality obligations with respect
to such Confidential Information no less onerous than those set forth in this Agreement) (collectively, “Recipients”) and (b) shall not use
Confidential Information of the Disclosing Party directly or indirectly for any purpose other than performing its obligations or exercising
its rights hereunder. The Receiving Party shall be jointly and severally liable for any breach by any of its Recipients of the restrictions set
forth in this Agreement. Notwithstanding the foregoing, trade secrets of the Disclosing Party shall be maintained by the Receiving Party
for so long as such information remains the trade secret of the Disclosing Party.

7.2         Exceptions to Confidentiality. The Receiving Party’s obligations set forth in this Agreement shall not extend to any

Confidential Information of the Disclosing Party:

like through no wrongful act, fault or negligence on the part of a Receiving Party or its Recipients;

(a)          that is or hereafter becomes part of the public domain by public use, publication, general knowledge or the

(b)          that is received from a third party without restriction and without breach of any agreement between such third

party and the Disclosing Party;

limitation on use or disclosure prior to its receipt from the Disclosing Party;

(c)          that the Receiving Party can demonstrate by competent evidence was already in its possession without any

(d)          that is generally made available to third parties by the Disclosing Party without restriction on disclosure; or

(e)          that the Receiving Party can demonstrate by competent, written evidence was independently developed by the

Receiving Party without the use of the Disclosing Party’s Confidential Information.

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7.3         Disclosure. Each Party may disclose Confidential Information to the extent that such disclosure is:

(a)          made in response to a valid order of a court of competent jurisdiction or other Regulatory Authority of a
country or any political subdivision thereof of competent jurisdiction; provided, however, that the Receiving Party shall first have given
notice to the Disclosing Party and given the Disclosing Party a reasonable opportunity to quash such order or to obtain a protective order
requiring  that  the  Confidential  Information  or  documents  that  are  the  subject  of  such  order  be  held  in  confidence  by  such  court  or
governmental body or, if disclosed, be used only for the purposes for which the order was issued; and provided further that if a disclosure
order  is  not  quashed  or  a  protective  order  is  not  obtained,  the  Confidential  Information  disclosed  in  response  to  such  court  or
governmental  order  shall  be  limited  to  that  information  that  is  legally  required  to  be  disclosed  in  such  response  to  such  court  or
governmental order;

(b)          otherwise required by law or regulation, in the reasonable opinion of legal counsel for the Receiving Party;
provided,  however,  the  Receiving  Party  must  promptly  give  the  Disclosing  Party  notice  of  any  such  disclosure  and  provide  the
Disclosing  Party  with  reasonable  assistance  in  obtaining  a  protective  order  with  respect  to  the  Confidential  Information  subject  to
disclosure;

(c)                    Intercept  may  disclose  Confidential  Information  to  the  extent  that  such  disclosure  is  made  to  Regulatory
Authorities as required in connection with any filing, application or request for Regulatory Approval; provided, however, that reasonable
measures shall be taken to assure confidential treatment of such information; or

(d)          To the extent, if any, that a Party concludes in good faith that it is required by applicable laws or regulations to
file  or  register  this  Agreement  or  a  notification  thereof  with  any  Regulatory  Authority,  including  the  U.S.  Securities  and  Exchange
Commission,  such  Party  may  do  so,  and  the  other  Party  shall  cooperate  in  such  filing  or  notification  and  shall  execute  all  documents
reasonably required in connection therewith. In such situation, the filing Party shall request confidential treatment of sensitive provisions
of the Agreement, to the extent permitted by Applicable Law and in consultation with the other Party. The Parties shall promptly inform
each other as to the activities or inquiries of any such Regulatory Authority relating to this Agreement, and shall cooperate to respond to
any request for further information therefrom.

7.4         Notification. The Receiving Party shall notify the Disclosing Party immediately, and cooperate with the Disclosing
Party as the Disclosing Party may reasonably request, upon the Receiving Party’s discovery of any loss or compromise of the Disclosing
Party’s Confidential Information.

7.5         Remedies.  Each  Party  agrees  that  the  unauthorized  use  or  disclosure  of  any  information  by  the  Receiving  Party  in
violation  of  this  Agreement  will  cause  severe  and  irreparable  damage  to  the  Disclosing  Party.  In  the  event  of  any  violation  of  this
ARTICLE 7, the Receiving Party agrees that the Disclosing Party shall be authorized and entitled to seek to obtain from any court of
competent jurisdiction injunctive relief, whether preliminary or permanent, as well as any other relief permitted by Applicable Law. The
Receiving Party agrees to waive any requirement that the Disclosing Party post bond as a condition for obtaining any such relief.

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7.6         Use of Names. Neither Party shall mention or otherwise use the name, insignia, symbol, trademark, trade name or
logotype of the other Party (or any abbreviation or adaptation thereof) in any publication, press release, promotional material or other
form of publicity without the prior written approval of such other Party in each instance. The restrictions imposed by this Section 7.6
shall  not  prohibit  either  Party  from  making  any  disclosure  identifying  the  other  Party  that  is  required  by  Applicable  Law;  provided,
however, that reasonable measures shall be taken to assure confidential treatment of such information.

7.7         Press Releases. Except as expressly provided in Section 7.3, neither Party shall make a press release or other public
announcement regarding this Agreement, the terms hereof or the transactions contemplated hereby without the prior written approval of
the other Party. Each Party shall provide the other with the proposed text of any such press release or public announcement for review
and approval, which approval shall not be unreasonably withheld, conditioned or delayed, as early as possible, but in no event less than
[**] Business Days in advance of the publication, communication or dissemination thereof; provided, however, that the receiving Party
shall be deemed to have approved any such press release or public announcement if it fails to notify the proposing Party in writing of any
objections to such press release or public announcement within [**] Business Days after receipt by the receiving Party of the text of such
public announcement.

ARTICLE 8
TERM AND TERMINATION

8.1         Term. This Agreement shall commence as of the Effective Date and, unless earlier terminated in accordance with the
terms  hereof,  shall  expire  on  December  31,  2020  (the  “Initial  Term”).  Thereafter,  this  Agreement  shall  automatically  renew  for
successive two (2)-year periods (each a “Renewal Period”) unless (a) Intercept provides notice to PharmaZell indicating its desire not to
renew at least twelve (12) months prior to the end of the Initial Term or then-current Renewal Period, as applicable, or (b) PharmaZell
provides notice to Intercept indicating its desire not to renew at least twelve (12) months prior to the end of the Initial Term or then-
current Renewal Period, as applicable. The Initial Term together with any Renewal Periods, shall be the “Term”.

8.2                  Termination.  In  addition  to  any  other  provision  of  this  Agreement  expressly  providing  for  termination  of  this

Agreement, this Agreement may be terminated as follows:

(a)          Intercept may terminate this Agreement immediately upon written notice to PharmaZell in the event that (i)
Regulatory  Authorities  require  or  cause  the  withdrawal  of  Product  or  if  the  Product  is  not  approved  by  the  FDA  and  the  European
Medicines Agency (EMA) or (ii) [**].

(b)          Intercept may terminate this Agreement immediately upon written notice to PharmaZell if (i) PharmaZell does
not deliver at least [**] of the amount of Supplied Material specified in a Work Order within [**] of the Delivery Date specified in such
Work Order or (ii) PharmaZell does not deliver at least [**] of Supplied Material in [**] provided that Intercept has ordered at least [**]
of Supplied Product for delivery in [**].

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(c)          This Agreement may be terminated by either Party:

(i)          immediately upon written notice if the other Party shall (A) file in any court or agency pursuant to
any  statute  or  regulation  of  any  state,  country  or  jurisdiction  a  petition  in  bankruptcy  or  insolvency  or  for  reorganization  or  for
arrangement or for the appointment of a receiver or trustee of that Party or of its assets, (B) propose a written agreement of composition
or extension of its debts, (C) be served with an involuntary petition against it, filed in any insolvency proceeding, and such petition shall
not  be  dismissed  within  [**]  days  after  the  filing  thereof,  (D)  propose  or  be  a  party  to  any  dissolution  or  liquidation,  (E)  make  an
assignment for the benefit of its creditors, or (F) admit in writing its inability generally to pay its debts as they fall due in the general
course;

(ii)                  immediately  upon  written  notice  in  the  event  of  any  material  breach  by  the  other  Party  in  the
performance of any of its obligations herein contained that (if curable) has not been cured by the defaulting Party within [**] days after
receiving written notice thereof from the non-breaching Party;

(iii)        immediately upon written notice in the event that, as a result of an order of government or any other
official authority, the continued operation of this Agreement in its entirety or in substantial part is prohibited or prevented or delayed for
an unspecified and indeterminate period; or

(iv)        as provided in Section 10.2.

(d)          Intercept may terminate this Agreement immediately upon written notice to PharmaZell in the event that (i)
any  audit  by  a  Regulatory  Authority  identifies  critical  or  major  finding  (as  defined  by  the  FDA  and/or  EMA)  at  a  Facility  and  such
critical  or  major  finding  is  not  remedied  by  PharmaZell  within  the  time  period  as  agreed  between  the  Regulatory  Authorities  and
PharmaZell or as mandated by the Regulatory Authorities after the identification thereof, (ii) PharmaZell fails to meet and/or maintain
the Quality Standards and does not remedy such failure within a reasonable time as agreed between Intercept and PharmaZell or, if no
agreement  is  reached  with  respect  to  such  time,  such  time  as  established  by  an  independent  auditor,  or  (iii)  any  audit  reveals  that  a
Facility is in violation of Applicable Laws.

8.3         Effect of Expiration or Termination.

(a)          The expiration or earlier termination of this Agreement shall be without prejudice to any rights or obligations
of the Parties that may have accrued prior to such termination. Those provisions that by their terms or intent are required to survive the
expiration or earlier termination of the Agreement in order to give effect to the intent of the Parties shall so survive. Without limiting the
foregoing, the provisions of Sections 4.5, 6.3 and 8.3 and ARTICLE 5, ARTICLE 7, ARTICLE 9 and ARTICLE 10 shall survive the
expiration  or  termination  of  this  Agreement  and  continue  thereafter  in  accordance  with  and  to  the  extent  of  their  terms.  Except  as
otherwise expressly provided herein, termination of this Agreement in accordance with the provisions hereof shall not limit remedies that
may otherwise be available at law or in equity.

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(b)          Upon expiration or earlier termination of this Agreement, each Party, at the request of the other, shall return
all data, files, records and other materials in its possession or Control containing or comprising the other Party’s Confidential Information
except that the legal department of such Party may retain one copy solely for archival purposes.

(c)          Upon any termination of this Agreement by Intercept pursuant to Section 8.2(a) or by PharmaZell pursuant to
Section 8.2(c), (i) PharmaZell shall return to Intercept all Intercept Materials, (ii) Intercept shall purchase from PharmaZell the amount of
Supplied Material that is subject to Work Orders outstanding at the time of such termination, (iii) Intercept shall reimburse PharmaZell
for  work  in  process  and  Materials  that  PharmaZell  has  purchased  for  the  purpose  of  supplying  Supplied  Material  to  Intercept  in
accordance  with  the  delivered  Work  Orders,  and  (iv)  Intercept  shall  pay  PharmaZell’s  direct  cost  for  any  such  work  in  process  in
accordance  with  the  Work  Orders  and  PharmaZell’s  purchase  price  from  its  suppliers  for  any  such  Materials  ordered  for  such  Work
Orders that have a minimum of [**] shelf life and have been stored and controlled by PharmaZell per the Quality Agreement; provided,
however that PharmaZell shall use reasonable best efforts to return such Materials to suppliers or use such Materials in the manufacture
of product for third parties. In the event of termination of this Agreement by Intercept pursuant to Section 8.2(b), 8.2(c) or 8.2(d), at the
request  of  Intercept,  PharmaZell  shall  fulfill  all  outstanding  Work  Orders  for  Supplied  Materials  prior  to  the  effective  date  of  such
termination  and  to  the  extent  not  used  to  fulfill  Work  Orders  at  Intercept’s  request,  PharmaZell  shall  return  to  Intercept  all  Intercept
Materials.

(d)          Except as and to the extent contemplated by Section 8.3(c), upon expiration of this Agreement or any earlier
termination of this Agreement, PharmaZell immediately shall cease all Manufacturing of Supplied Materials pursuant to this Agreement.

(e)                    Following  expiration  or  termination  of  this  Agreement,  PharmaZell  shall  (i)  provide  Intercept  with  such
reasonable  cooperation  and  support  with  respect  to  regulatory  matters  as  Intercept  may  require  in  order  to  dispose  of  previously
purchased  API,  (ii)  grant  to  Intercept  a  perpetual,  irrevocable,  non-exclusive  royalty-free  license  (with  the  right  to  grant  sublicenses)
under  know-how,  patents  and  other  intellectual  property  rights  owned,  licensed  or  otherwise  controlled  by  PharmaZell  (or  any  of  its
Affiliates) as may be necessary or useful for the purpose of making and having made the API and API Precursor and (iii) within thirty
(30)  days  of  such  expiration  or  termination,  provide  to  Intercept  copies  of  the  physical  embodiment  of  those  processes,  protocols,
procedures, methods, tests and other know-how, relating to the Manufacturing of the API and API Precursor. In addition, PharmaZell
shall  provide  reasonable  assistance  to  Intercept  and  its  Affiliates  with  respect  to  assisting  Intercept  and  its  Affiliates  in  obtaining  all
necessary regulatory approvals and/or modifying existing Regulatory Approvals for the Manufacture of the API.

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ARTICLE 9
INDEMNIFICATION

9.1         PharmaZell Indemnification. PharmaZell shall indemnify Intercept, its Affiliates and sublicensees and its and their
respective directors, officers, employees and agents (the “Intercept Indemnified Parties”), and defend and hold each of them harmless,
from  and  against  any  and  all  claims,  lawsuits,  actions,  suits  and  demands  brought  by  a  third  party  (a  “Third  Party  Claim”)  and  all
associated  losses,  damages,  liabilities,  penalties,  costs  and  expenses  (including  reasonable  attorneys’  fees  and  disbursements)
(collectively, “Losses”)  incurred  by  any  of  them  arising  from  or  occurring  as  a  result  of  (a)  the  breach  by  PharmaZell  of  any  of  its
representations  or  warranties  set  forth  in  this  Agreement,  (b)  PharmaZell’s  breach  of  any  of  its  covenants  or  obligations  under  this
Agreement, (c) PharmaZell’s gross negligence or willful misconduct in the performance of this Agreement, (d) the storage, release, or
disposal  of  any  hazardous  or  regulated  material  or  any  waste  by  PharmaZell,  (e)  violation  of  Applicable  Law  by  any  PharmaZell
Indemnitee,  or  (f)  the  enforcement  by  Intercept  of  its  rights  under  this  Section  9.1,  except,  in  each  case,  for  those  Losses  for  which
Intercept has an obligation to indemnify the PharmaZell Indemnified Parties pursuant to Section 9.2, as to which Losses each Party shall
indemnify the other Party to the extent of its respective liability for such Losses.

9.2         Intercept Indemnification. Intercept shall indemnify PharmaZell, its Affiliates and its and their respective directors,
officers, employees and agents (the “PharmaZell Indemnified Parties”), and defend and hold each of them harmless, from and against
any and all Third Party Claims and all associated Losses incurred by any of them arising from or occurring as a result of (a) the breach
by Intercept of any of its representations or warranties set forth in this Agreement, (b) Intercept’s breach of its covenants or obligations
under this Agreement, (c) violation of Applicable Law by any Intercept Indemnitee, or (d) the enforcement by PharmaZell of its rights
under  this  Section  9.2,  except,  in  each  case,  for  those  Losses  for  which  PharmaZell  has  an  obligation  to  indemnify  the  Intercept
Indemnified Parties pursuant to Section 9.1, as to which Losses each Party shall indemnify the other Party to the extent of its respective
liability for such Losses.

9.3         Indemnification Procedure.

(a)          Notice of Claim. The indemnified party (the “Indemnified Party”) shall give the indemnifying Party (the
“Indemnifying  Party”)  prompt  written  notice  (an  “Indemnification  Claim  Notice”)  of  any  Third  Party  Claims  and  the  associated
Losses or discovery of facts upon which such Indemnified Party intends to base a request for indemnification under Section 9.1 or 9.2,
but  in  no  event  shall  the  Indemnifying  Party  be  liable  for  any  Losses  that  result  from  any  delay  in  providing  such  notice.  Each
Indemnification  Claim  Notice  must  contain  a  description  of  the  claim  and  the  nature  and  amount  of  such  Loss  (to  the  extent  that  the
nature and amount of such Loss are known at such time). The Indemnified Party shall furnish promptly to the Indemnifying Party copies
of all papers and official documents received in respect of any Losses.

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(b)          Control of Defense. At its option, the Indemnifying Party may assume the defense of any Third Party Claim
by giving written notice to the Indemnified Party within [**] days after the Indemnifying Party’s receipt of an Indemnification Claim
Notice. The assumption of the defense of a Third Party Claim by the Indemnifying Party shall not be construed as an acknowledgment
that  the  Indemnifying  Party  is  liable  to  indemnify  any  Indemnified  Party  in  respect  of  the  Third  Party  Claim,  nor  shall  it  constitute  a
waiver  by  the  Indemnifying  Party  of  any  defenses  it  may  assert  against  any  Indemnified  Party’s  claim  for  indemnification.  Upon
assuming the defense of a Third Party Claim, the Indemnifying Party may appoint as lead counsel in the defense of the Third Party Claim
any legal counsel selected by the Indemnifying Party, which shall be reasonably acceptable to the Indemnified Party. In the event the
Indemnifying Party assumes the defense of a Third Party Claim, the Indemnified Party shall immediately deliver to the Indemnifying
Party all original notices and documents (including court papers) received by any Indemnified Party in connection with the Third Party
Claim. Subject to Section 9.3(c), if the Indemnifying Party assumes the defense of a Third Party Claim, the Indemnifying Party shall not
be  liable  to  the  Indemnified  Party  for  any  legal  expenses  subsequently  incurred  by  such  Indemnified  Party  in  connection  with  the
analysis, defense or settlement of the Third Party Claim. In the event that it is ultimately determined that the Indemnifying Party is not
obligated to indemnify, defend or hold harmless a Intercept Indemnified Party or PharmaZell Indemnified Party, as applicable, from and
against  the  Third  Party  Claim,  the  Indemnified  Party  shall  reimburse  the  Indemnifying  Party  for  any  and  all  costs  and  expenses
(including reasonable attorneys’ fees and costs of suit) and any Losses incurred by the Indemnifying Party in its defense of the Third
Party Claim with respect to such Intercept Indemnified Party or PharmaZell Indemnified Party, as applicable.

(c)          Right to Participate in Defense. Without limiting Section 9.3(b), any Indemnified Party shall be entitled to
participate in, but not control, the defense of such Third Party Claim and to employ counsel of its choice for such purpose; provided,
however, that such employment shall be at the Indemnified Party’s own expense unless (A) the employment thereof has been specifically
authorized  by  the  Indemnifying  Party  in  writing,  (B)  the  Indemnifying  Party  has  failed  to  assume  the  defense  and  employ  counsel  in
accordance with Section 9.3(b) (in which case the Indemnified Party shall control the defense), or (C) the interests of the Indemnified
Party and the Indemnifying Party with respect to such Third Party Claim are sufficiently adverse to prohibit the representation by the
same counsel of both Parties under applicable law, ethical rules or equitable principles.

(d)          Settlement. With respect to any Losses relating solely to the payment of money damages in connection with a
Third  Party  Claim,  without  any  admission  of  liability  or  fault,  and  that  will  not  result  in  the  Indemnified  Party’s  becoming  subject  to
injunctive  or  other  relief  or  otherwise  adversely  affect  the  business  of  the  Indemnified  Party  in  any  manner,  and  as  to  which  the
Indemnifying Party shall have acknowledged in writing the obligation to indemnify the Indemnified Party hereunder, the Indemnifying
Party shall have the sole right to consent to the entry of any judgment, enter into any settlement or otherwise dispose of such Loss, on
such terms as the Indemnifying Party, in its sole discretion, shall deem appropriate. With respect to all other Losses in connection with
Third Party Claims, where the Indemnifying Party has assumed the defense of the Third Party Claim in accordance with Section 9.3(b),
the Indemnifying Party shall have authority to consent to the entry of any judgment, enter into any settlement or otherwise dispose of
such Loss; provided that it obtains the prior written consent of the Indemnified Party (which consent shall not be unreasonably withheld,
conditioned or delayed). The Indemnifying Party shall not be liable for any settlement or other disposition of a Loss by an Indemnified
Party that is reached without the written consent of the Indemnifying Party. Regardless of whether the Indemnifying Party chooses to
defend  or  prosecute  any  Third  Party  Claim,  no  Indemnified  Party  shall  admit  any  liability  with  respect  to,  or  settle,  compromise  or
dispose of, any Third Party Claim without the prior written consent of the Indemnifying Party (which consent shall not be unreasonably
withheld, conditioned or delayed).

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(e)                    Cooperation.  If  the  Indemnifying  Party  chooses  to  defend  or  prosecute  any  Third  Party  Claim,  the
Indemnified  Party  shall  cooperate  in  the  defense  or  prosecution  thereof  and  shall  furnish  such  records,  information  and  testimony,
provide such witnesses and attend such conferences, discovery proceedings, hearings, trials and appeals as may be reasonably requested
in connection therewith. Such cooperation shall include access during normal business hours afforded to the Indemnifying Party to, and
reasonable retention by the Indemnified Party of, records and information that are reasonably relevant to such Third Party Claim, and
making employees and agents available on a mutually convenient basis to provide additional information and explanation of any material
provided hereunder, and the Indemnifying Party shall reimburse the Indemnified Party for all its reasonable out-of-pocket expenses in
connection therewith.

(f)           Expenses. Except as provided above, the reasonable and verifiable costs and expenses, including fees and
disbursements of counsel, incurred by the Indemnified Party in connection with any Third Party Claim shall be reimbursed on a calendar
quarter basis in arrears by the Indemnifying Party, without prejudice to the Indemnifying Party’s right to contest the Indemnified Party’s
right to indemnification and subject to refund in the event the Indemnifying Party is ultimately held not to be obligated to indemnify the
Indemnified Party.

9.4         Insurance.

(a)          During the Term, each Party shall maintain adequate liability insurance covering its activities and obligations
under  this  Agreement  that  is  standard  and  reasonable  in  the  biopharmaceutical  industry  for  companies  conducting  similar  activities;
provided that for PharmaZell in no event shall such amounts be less than (i) with respect to comprehensive general liability insurance, a
combined  single  limit  for  bodily  injury  and  property  damage  of  not  less  than  [**]and  (ii)  with  respect  to  product  liability/completed
operations coverage, a per claim limit of not less than [**] (collectively, the “Policies”). If any Policy is written on a claims-made basis,
the retroactive date, if any, shall not be later than the Effective Date and such coverage shall be continued for a period of [**] following
the Term. Each Party shall provide prompt notice to the other Party in the event that the first Party’s Policies are canceled or subjected to
a reduction of coverage or any other material adverse modification.

Effective Date.

(b)          Each Party shall furnish certificates of insurance for its Policies to the other Party within [**] days after the

9.5         Limitation on Damages. IN NO EVENT SHALL: (A) EITHER PARTY BE LIABLE TO THE OTHER PARTY FOR
SPECIAL,  PUNITIVE,  INDIRECT,  INCIDENTAL,  EXEMPLARY  OR  CONSEQUENTIAL  DAMAGES,  INCLUDING  BUSINESS
INTERRUPTION OR LOST PROFITS, WHETHER IN CONTRACT, WARRANTY, NEGLIGENCE, TORT, STRICT LIABILITY OR
OTHERWISE AND (B) EITHER PARTY’S LIABILITY EXCEED FIFTEEN MILLION UNITED STATES DOLLARS ($15,000,000)
ON  A  PER  CLAIM  BASIS.  THE  FOREGOING  LIMITATIONS  AND  EXCLUSIONS  ARE  NOT  INTENDED  TO,  NOR  SHALL
THEY,  EXCLUDE  OR  LIMIT  DAMAGES  OR  CLAIMS  CAUSED  BY  A  PARTY’S  GROSS  NEGLIGENCE,  WILLFUL
MISCONDUCT OR BREACH OF THE PROVISIONS OF ARTICLE 5, OR EXCLUDE OR LIMIT A PARTY’S INDEMNIFICATION
OBLIGATIONS UNDER SECTION 9.1 OR 9.2.

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ARTICLE 10
MISCELLANEOUS

10.1              Notices.  All  notices,  requests  and  other  communications  hereunder  must  be  in  writing,  specifically  reference  this
Agreement in a prominent manner, and be delivered personally, sent by first class registered or certified mail, postage prepaid, return
receipt  requested  or  by  internationally  recognized  overnight  delivery  service  that  maintains  records  of  delivery  to  the  Parties  at  the
following addresses:

If to Intercept to:

Intercept Pharma Europe Ltd.
2 Pancras Square, Floor 1, London
United Kingdom N1C 4AG
Attention: [**]

with copies (which shall not constitute notice) to:

Intercept Pharma Europe Ltd.
2 Pancras Square, Floor 1, London
United Kingdom N1C 4AG
Attention: Head of Legal

and

Intercept Pharmaceuticals, Inc.
450 W 15th St,
Suite 505 Floor 5
New York, NY 10011
Attention: General Counsel

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If to PharmaZell to:

PharmaZell GmbH
Rosenheimer Straβe 43
83064 Raubling
Germany
Attention: [**]

All such notices, requests and other communications will (a) if delivered personally to the address as provided in this Section, be deemed
given upon delivery, (b) if delivered by internationally recognized overnight delivery courier be deemed given on the second Business
Day (at the place of delivery) after deposit with such internationally recognized delivery service, (c) if sent by first class registered or
certified  mail,  postage  prepaid,  return  receipt  requested,  within  the  United  States,  on  the  third  Business  Day  following  the  date  of
mailing, and (d) if sent by international first class registered or certified mail, postage prepaid, return receipt requested, on the seventh
Business Day following the date of mailing. Any Party from time to time may change its address or other information for the purpose of
notices to that Party by giving notice specifying such change to the other Party hereto.

10.2       Force Majeure. Neither Party shall be liable for delay in delivery or nonperformance in whole or in part, nor shall the
other Party have the right to terminate this Agreement except as otherwise specifically provided in this Section 10.2, where delivery or
performance has been affected by fires, floods, embargoes, strikes, epidemics, quarantines, war, acts of war (whether war be declared or
not),  terrorism,  insurrections,  riots,  civil  commotion,  acts  of  God  or  acts  or  similar  condition  beyond  such  Party’s  reasonable  control;
provided that the Party affected by such a condition shall, within [**] days of its occurrence, give notice to the other Party stating the
nature  of  the  condition,  its  anticipated  duration  and  any  action  being  taken  to  avoid  or  minimize  its  effect.  The  suspension  of
performance  shall  be  of  no  greater  scope  and  no  longer  duration  than  is  reasonably  required  and  the  nonperforming  Party  shall  use
commercially  reasonable  efforts  to  remedy  its  inability  to  perform.  Notwithstanding  the  foregoing,  in  the  event  the  suspension  of
performance continues for [**] days after the date of the occurrence, and such failure to perform would constitute a material breach of
this Agreement in the absence of such force majeure event, the nonaffected Party may terminate this Agreement immediately by written
notice to the affected Party.

10.3       Entire Agreement; Amendment.

(a)          This Agreement, together with the Schedules and Exhibits attached hereto and the Quality Agreement, which
shall  be  incorporated  by  reference  hereto,  sets  forth  and  constitutes  the  entire  agreement  and  understanding  between  the  Parties  with
respect to the subject matter hereof and all prior agreements (including any terms and conditions previously agreed upon by the Parties),
understandings, promises and representations, whether written or oral, with respect thereto are superseded hereby. Each Party confirms
that it is not relying on any representations or warranties of the other Party except as specifically set forth herein.

executed by authorized representatives of both Parties.

(b)          No amendment, modification, release or discharge shall be binding upon the Parties unless in writing and duly

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10.4       Further Assurances. Each Party shall duly execute and deliver, or cause to be duly executed and delivered, such further
instruments and do and cause to be done such further acts and things, including the filing of such assignments, agreements, documents
and instruments as may be necessary or as the other Party may reasonably request in connection with this Agreement or to carry out more
effectively the provisions and purposes hereof or to better assure and confirm unto such other Party its rights and remedies under this
Agreement.

10.5       Successors and Assigns. The terms and provisions hereof shall inure to the benefit of, and be binding upon, Intercept,

PharmaZell and their respective successors and permitted assigns.

10.6       Governing Law. This Agreement shall be governed and interpreted in accordance with the laws of England and Wales,
excluding any conflicts or choice of law rule or principle that might otherwise refer construction or interpretation of this Agreement to
the substantive law of another jurisdiction; provided, however, for all intellectual property matters, this Agreement shall be governed and
interpreted in accordance with the laws of New York, New York, excluding any conflicts or choice of law rule or principle that might
otherwise refer construction or interpretation of this Agreement to the substantive law of another jurisdiction. To the extent not resolved
pursuant  to  Section  10.7  or  Section  10.8,  venue  for  any  litigation  between  the  Parties  shall  be  London,  England  or,  with  respect  to
intellectual property matters, New York, New York. The Parties agree to exclude the application to this Agreement of the United Nations
Convention on Contracts for the International Sale of Goods.

10.7       Dispute Resolution.

(a)          In the event of a dispute between the Parties, either Party may, by giving written notice of dispute to the other
Party,  request  a  meeting  of  authorized  representatives  of  the  Parties  for  the  purpose  of  resolving  the  dispute.  The  Parties  agree  that,
within [**] days after any such request, each Party shall designate a representative to participate in dispute resolution discussions that
shall be held in [**] at a mutually acceptable time for the purpose of resolving the dispute. Each Party agrees to negotiate in good faith to
resolve the dispute in a mutually acceptable manner.

(b)          If for whatever reason the Parties are unable to resolve the dispute within [**] days after the issuance of a
notice of dispute, then either Party may, by written notice to the other Party, submit the dispute to binding arbitration in accordance with
the provisions of Section 10.8, except for those disputes excluded from Section 10.8 which shall be subject to the provisions of Section
10.6.

10.8       Arbitration.

(a)          Except to the extent otherwise provided in Section 4.5, Section 7.5, or arising out of a dispute relating to
Article 5, any dispute arising out of or relating to this Agreement, including the breach, termination or validity thereof, shall, after first
being subject to negotiations between the Parties as provided in Section 10.7(a), be finally resolved by arbitration in accordance with the
Rules of Conciliation and Arbitration of the International Chamber of Commerce (“ICC Rules”) as then in effect, provided that, in the
event and to the extent such rules conflict with the terms of this Section 10.8, the terms of this Section 10.8 shall govern. Judgment on
the award rendered by the arbitrator(s) may be entered in any court having jurisdiction thereof. The place of arbitration shall be [**]. The
arbitration shall be conducted in the English language. The place of litigation for disputes relating to Article 5 shall be [**].

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(b)          Except as provided in Section 10.8(c), the arbitration shall be held before a single arbitrator, who shall be
selected  by  agreement  of  the  Parties,  or,  if  the  Parties  cannot  agree  within  [**]  days  after  commencement  of  arbitration,  then  by  the
International Chamber of Commerce. The arbitrator selected pursuant to this Section 10.8(c) shall be a practicing or retired lawyer or
retired judge and have experience relating to agreements concerning the marketing of pharmaceutical products in the United States.

(c)          Notwithstanding Section 10.8(b), in the event that the dispute that is subject to arbitration is one in which a
Party  seeks  to  recover  an  amount  of  at  least  [**]  from  the  other  Party,  then  either  Party  shall  have  the  option,  exercisable  by  written
notice to the other Party given at any time within [**] days after commencement of arbitration, to require that the arbitration be held
before a panel of three (3) arbitrators. In such case, within [**] days after the provision of notice described in the preceding sentence,
each Party shall select one person to act as arbitrator. If a Party shall fail within the designated time period to select an arbitrator, then the
arbitrator to be selected by the Party shall be selected by the International Chamber of Commerce. The two (2) persons so selected as
arbitrators shall select a third arbitrator within [**] days of their appointment. If the two (2) initially selected arbitrators are unable or fail
to  agree  upon  the  third  arbitrator,  the  third  arbitrator  shall  be  selected  by  the  International  Chamber  of  Commerce.  Each  arbitrator
selected  pursuant  to  this  Section  10.8(c)  shall  be  a  practicing  lawyer  or  retired  judge  and  have  experience  relating  to  agreements
concerning the marketing of pharmaceutical products in the United States.

(d)          Each Party shall, upon the written request of the other Party, promptly provide the other Party with copies of
documents relevant to the issues raised by the dispute on which the producing Party may rely in support of, or in opposition to, any claim
or  defense.  Any  dispute  regarding  discovery,  or  the  relevance  or  scope  thereof,  shall  be  determined  by  the  arbitrator(s),  which
determination  shall  be  conclusive.  To  the  extent  reasonable  under  the  circumstances  and  as  agreed  in  writing  by  the  Parties,  all
discoveries shall be completed within [**] days following the appointment of the arbitrator(s).

(e)          It is the intent of the Parties that, barring extraordinary circumstances, and to the extent reasonable, arbitration
proceedings will be concluded within [**] months from the date the arbitrator is appointed (or, where a panel of three (3) arbitrators is
used, within [**] months from the date upon which the third arbitrator is appointed). The arbitrator(s) may extend this time limit in the
interests of justice. Failure to adhere to this time limit shall not constitute a basis for challenging the award.

(f)           Except as may be required by Applicable Law (including applicable securities laws or rules of a securities
exchange) or as may be necessary to enforce the arbitration award or the provisions of this Section 10.8, and except for disclosures made
by a Party to its accountants, insurers, consultants, or attorneys or to actual or potential lenders, non-public investors, rating agencies,
acquirers, or business partners who are under obligations to the disclosing Party to hold the disclosed information in confidence, neither a
Party nor its representatives may disclose the existence, content, or results of any arbitration hereunder without the prior written consent
of the other Party.

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(g)          The arbitrator(s) shall have discretion to allocate the Parties’ costs and expenses for the arbitration (including
attorneys’ fees), the fees of the arbitrator(s), and the administrative fees of arbitration between the Parties in proportion to the extent to
which  they  prevail.  Failing  such  allocation,  each  Party  shall  bear  its  own  costs  and  expenses  and  an  equal  share  of  the  fees  of  the
arbitrators and administrative fees of the arbitration.

10.9       Third Party Beneficiaries. Nothing in this Agreement shall be construed as giving any Person, other than the Parties
hereto  and  their  successors  and  permitted  assigns,  any  right,  remedy  or  claim  under  or  in  respect  of  this  Agreement  or  any  provision
hereof.

10.10          Export Control.  This  Agreement  is  made  subject  to  any  restrictions  concerning  the  export  of  products  or  technical
information from the United States or other countries that may be imposed on the Parties from time to time. Each Party agrees that it will
not export, directly or indirectly, any technical information acquired from the other Party under this Agreement or any products using
such  technical  information  to  a  location  or  in  a  manner  that  at  the  time  of  export  requires  an  export  license  or  other  governmental
approval, without first obtaining the written consent to do so from the appropriate agency or other governmental entity in accordance
with Applicable Law.

10.11          Assignment.  Except  as  expressly  provided  herein,  neither  Party  may,  without  the  prior  written  consent  of  the  other
Party, sell, transfer, assign, delegate, pledge, subcontract or otherwise dispose of, whether voluntarily, involuntarily, by operation of law
or otherwise, this Agreement or any of its rights or duties hereunder; provided, however, that (a) Intercept may, without such consent,
assign this Agreement and its rights and obligations hereunder to an Affiliate, (b) Intercept may, without such consent, assign its rights
and delegate its obligations under this Agreement in respect of Supplied Materials to the purchaser or sublicensee of Intercept’s rights in
and to such Supplied Materials or the relevant Product, (c) PharmaZell may, without such consent, assign this Agreement and its rights
and obligations hereunder to one or more Affiliates, and (d) either Party may, without such consent, assign this Agreement and its rights
and obligations hereunder to the purchaser of all or substantially all of its assets or to any successor entity or acquirer in the event of a
merger,  consolidation  or  change  in  control  of  such  Party.  Any  attempt  to  assign,  transfer,  subcontract  or  delegate  any  portion  of  this
Agreement in violation of this Section 10.11 shall be null and void. In the event either Party assigns all of its rights and delegates all of
its obligations under this Agreement to another Person in accordance with the terms hereof and the assignee/delegee acquires all rights
and  assumes  all  obligations  of  its  assignor/delegor  under  this  Agreement,  then  the  assignor/delegor  shall  cease  to  be  a  party  to  this
Agreement or to have any rights or obligations under this Agreement from and after the effective date of such assignment or delegation.
Except as provided in the preceding sentence, no assignment or delegation shall relieve the assignor or delegor of any of its obligations
hereunder.

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10.12     Waiver. Any term or condition of this Agreement may be waived at any time by the Party that is entitled to the benefit
thereof, but no such waiver shall be effective unless set forth in a written instrument duly executed by or on behalf of the Party waiving
such term or condition. No waiver by either Party of any term or condition of this Agreement, in any one or more instances, shall be
deemed to be or construed as a waiver of the same or any other term or condition of this Agreement on any future occasion.

10.13     Severability. If any provision of this Agreement is held to be illegal, invalid or unenforceable under any present or
future law, and if the rights or obligations of either Party under this Agreement will not be materially and adversely affected thereby,
(a) such provision shall be fully severable, (b) this Agreement shall be construed and enforced as if such illegal, invalid or unenforceable
provision had never comprised a part hereof, (c) the remaining provisions of this Agreement shall remain in full force and effect and
shall not be affected by the illegal, invalid or unenforceable provision or by its severance herefrom, and (d) in lieu of such illegal, invalid
or unenforceable provision, there shall be added automatically as a part of this Agreement a legal, valid and enforceable provision as
similar in terms to such illegal, invalid or unenforceable provision as may be possible and reasonably acceptable to the Parties herein.

10.14          Independent Contractors.  The  status  of  the  Parties  under  this  Agreement  shall  be  that  of  independent  contractors.
Nothing  in  this  Agreement  is  intended  or  shall  be  deemed  to  constitute  a  partnership,  agency,  employer,  employee,  or  joint  venture
relationship between the Parties. Neither Party shall have the right to enter into any agreements on behalf of the other Party, nor shall it
represent to any Person that it has any such right or authority.

10.15     Construction.  Unless  the  context  of  this  Agreement  otherwise  requires:  (a)  words  of  any  gender  include  each  other
gender; (b) words using the singular or plural number also include the plural or singular number, respectively; (c) the terms “hereof,”
“herein,”  “hereby”  and  derivative  or  similar  words  refer  to  this  entire  Agreement;  (d)  the  terms  “Article,”  “Section,”  “Schedule,”
“Exhibit” or “clause” refer to the specified Article, Section, Schedule, Exhibit or clause of this Agreement; (e) the term “or” has, except
where  otherwise  indicated,  the  inclusive  meaning  represented  by  the  phrase  “and/or”;  (f)  the  term  “including”  or  “includes”  means
“including without limitation” or “includes without limitation”; and (g) references to any agreement, instrument or other document in this
Agreement  refer  to  such  agreement,  instrument  or  other  document  as  originally  executed  or,  if  subsequently  amended,  replaced  or
supplemented  from  time  to  time,  as  so  amended,  replaced  or  supplemented  and  in  effect  at  the  relevant  time  of  reference  thereto.
Whenever this Agreement refers to a number of days, such number shall refer to calendar days unless Business Days are specified. The
captions of this Agreement are for convenience of reference only and in no way define, describe, extend, or limit the scope or intent of
this Agreement or the intent of any provision contained in this Agreement. The language of this Agreement shall be deemed to be the
language mutually chosen by the Parties and no rule of strict construction shall be applied against either Party.

10.16          Remedies.  The  rights  and  remedies  provided  herein  are  cumulative  and  do  not  exclude  any  other  right  or  remedy

provided by applicable law or otherwise available except as expressly set forth herein.

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10.17     Counterparts; Facsimile Execution. This Agreement may be executed in any number of counterparts, each of which
shall be deemed to be an original, and all of which, taken together, shall constitute one and the same instrument. Delivery of an executed
counterpart of a signature page of this Agreement (and each amendment, modification and waiver in respect of it) by facsimile or other
electronic transmission shall be as effective as delivery of a manually executed original counterpart of each such instrument.

10.18          English  Language.  This  Agreement  shall  be  written  and  executed  in,  and  all  other  communications  under  or  in
connection with this Agreement shall be in, the English language. Any translation into any other language shall not be an official version
thereof,  and  in  the  event  of  any  conflict  in  interpretation  between  the  English  version  and  such  translation,  the  English  version  shall
control.

10.19          Parent  Guarantee.  Intercept  Parent  hereby  agrees  to  be  jointly  and  severally  liable  for  the  prompt  and  complete
performance of Intercept’s financial obligations under this Agreement, and hereby guarantees the financial performance by Intercept of
the obligations set forth in this Agreement.

[Signature Page Follows]

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IN WITNESS WHEREOF, the Parties hereto have executed this Agreement to be effective as of the last date of signature below.

INTERCEPT PHARMA EUROPE LTD.

    PHARMAZELL GmbH

By:

/s/ Steve Arnold

Name: Steve Arnold

Title: SVP

  By:

/s/ Oliver Bolzern

  Name: Oliver Bolzern

  Title: CEO

Date: August 12, 2016

  Date: August 12, 2016

AGREED TO AND ACCEPTED SOLELY FOR PURPOSES OF
SECTION 10.19:

INTERCEPT PHARMACEUTICALS, INC.

By:

/s/ Sandip Kapadia

Name: Sandip Kapadia

Title: CFO

Date: August 12, 2016

[Signature Page to Manufacturing and Supply Agreement]

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
SCHEDULE 1.40

Intercept Materials

[**]

Schedule 1.40 to Manufacturing and Supply Agreement

SCHEDULE 1.83

Form of Work Order

FOR ILLUSTRATION PURPOSES ONLY – DO NOT EXECUTE

WORK ORDER #____

This  Work  Order  #____  (“Work  Order”)  is  entered  into  and  effective  with  and  as  of  the  last  signature  to  it  by  either  Party  by  and
between  Intercept  Pharma  Europe  Ltd.  (“Intercept”)  and  PharmaZell  GmbH  (“PharmaZell”)and  is  subject  to  all  of  the  terms  and
conditions of the Manufacturing and Supply Agreement between Intercept and PharmaZell, effective as of ____, 2016 (the “Agreement”)
and in accordance with this Work Order using, if applicable, the materials provided by Intercept hereunder.

Specifications supplied by Intercept: as in Quality Agreement signed September 12, 2014

Description  of  Services  or  Scope  of  Work:  PharmaZell  shall  provide  the  following  Supplied  Material  to  Intercept:  Work  Order
Description. [Or insert Description, including any work product, reports, or presentations contemplated under this Agreement; please be
as specific as possible] or [If applicable, “as outlined in Appendix 1 attached hereto and incorporated by reference.”]

Deliverables: Quantity of Supplied Materials.

Delivery Date: [Insert desired Delivery Date]

Place of Delivery: [Insert desired Delivery location]

Timelines and Milestones: PharmaZell will provide schedule and progress updates in accordance with the terms of the Agreement.

Compensation: Intercept shall pay the total sum not to exceed of Total Estimated Work Amount (the “Total Fee”) in accordance with
the  commercial  pricing  set  forth  in  the  Agreement  and  in  consideration  for  the  performance  of  the  above  Supplied  Material  supplied.
Payment shall be made in accordance with the details outlined in the Agreement.

OTHER TERMS TO BE ADDED AS AGREED

Capitalized  terms  contained  in  this  Work  Order  and  not  otherwise  defined  herein,  shall  have  the  meaning  ascribed  to  them  in  the
Agreement.

This Work Order may be executed in counterparts, each of which shall be deemed an original, but all of which together shall be deemed
to  be  one  and  the  same  agreement.  A  signed  copy  of  this  Work  Order  delivered  by  facsimile,  e-mail  or  other  means  of  electronic
transmission shall be deemed to have the same legal effect as delivery of an original signed copy of this Agreement.

[Remainder of Page Intentionally Blank]

Schedule 1.83 to Manufacturing and Supply Agreement

1

IN WITNESS WHEREOF, each Party has executed this Work Order by a duly authorized individual effective as of the later of

the signatures below.

INTERCEPT PHARMA EUROPE LTD.

     PHARMAZELL GMBH

Form Only – Do Not Sign

By:
Name: 
Title:
Date:  

Form Only – Do Not Sign

  By:
  Name:  
Title:
  Date:

Schedule 1.83 to Manufacturing and Supply Agreement

2

 
 
 
 
 
 
 
 
 
SCHEDULE 2.1(d)

Approved Subcontractors and Activities

Subcontractor

Activity

[**]  

[**]  

[**]  

[**]  

Schedule 2.1(d) to Manufacturing and Supply Agreement

[**]

[**]

[**]

[**]

    
 
 
 
 
SCHEDULE 2.2(a)

Existing Work Orders

[**]

Schedule 2.2(a) to Manufacturing and Supply Agreement

Schedule 2.2(b)

First New Work Order

[**]

Schedule 2.2(b) to Manufacturing and Supply Agreement

SCHEDULE 2.7(e)

Standard Yields

[**]

Schedule 2.7(e) to Manufacturing and Supply Agreement

EX-10.41 14 v324396_ex10-41.htm EXHIBIT 10.41

Exhibit 10.41

EXECUTION COPY

Certain identified information has been excluded from this exhibit because it is both not 
material and would likely cause competitive harm to the registrant if publicly disclosed.

LICENSE AGREEMENT

This  License  Agreement  (this  “Agreement”),  dated  as  of  March  29,  2011  (the  “Effective  Date”),  is  made  by  and  between
DAINIPPON SUMITOMO PHARMA CO. LTD., a company organized under the laws of Japan (“DSP”), having a place of business at
6-8  Doshomachi  2-chome,  Chuo-ku,  Osaka  541-0045  Japan,  and  INTERCEPT  PHARMACEUTICALS,  INC.,  a  company  organized
under the laws of the State of Delaware (“Intercept”), having a place of business at 18 Desbrosses Street, New York, New York 10013.
DSP and Intercept are sometimes referred to herein individually as a “Party” and collectively as the “Parties.”

RECITALS

WHEREAS,  Intercept  is  a  clinical  stage  biopharmaceutical  company  engaged  in  the  development  of  therapeutics  for  the
treatment of metabolic diseases, and is currently developing Obeticoholic acid, a farnesoid X receptor (FXR) agonist, more commonly
known  as  6α-ethyl-3α,7α-dihydroxy-5β-cholan-24-oic  acid  (6-ECDCA)  or  INT-747,  in  any  form  (the  “Compound”)to  be  used  to
formulate  a  new  product  for  therapeutic  use  in  connection  with  primary  biliary  cirrhosis  (“PBC”)  and  nonalcoholic  steatohepatitis
(“NASH”) (PBC and NASH, collectively the “Field”);

WHEREAS,  Intercept  is  simultaneously  engaged  in  the  development  of  other  indications  for  the  Compound,  including  in
connection with portal hypertension (together with all present and future indications of the Compound, each an “Additional Indication”,
and collectively, the “Additional Indications”);

WHEREAS, DSP is a worldwide pharmaceutical company that has significant experience in the development, manufacturing

and commercialization of pharmaceutical products in the Territory (as defined hereinafter); and

WHEREAS,  Intercept  desires  to  grant  certain  exclusive  rights  to  DSP  in  the  Territory  with  respect  to  the  development,
manufacturing and commercialization of the Compound and the Product in the Field in the Territory and DSP wishes to accept the grant
of such rights; all as more particularly set forth in this Agreement.

NOW THEREFORE, in consideration of the foregoing premises and the mutual promises, covenants and conditions contained

in this Agreement, the Parties agree as follows:

1.          DEFINITIONS

Whenever  used  in  the  Agreement  with  an  initial  capital  letter,  the  terms  defined  in  this  Article  1  shall  have  the  meanings

specified below.

“Actual Costs” shall mean Intercept’s direct costs and indirect costs incurred by sub-contractors of Intercept of materials and
labor  specifically  incurred  in  Manufacturing  or  formulating  the  Clinical  Supplies  or  Commercial  Supplies  supplied  to  DSP  under  the
Clinical Supply Agreement or the Commercial Supply Agreement, including but not limited to excipients and packaging components for
both  the  Compound  and  the  Product,  as  well  as  in  process  and  release  testing,  stability  testing,  development  of  the  Specifications,
manufacturing validation, quality assurance and quality control activities necessary to release the Compound or Product to DSP or to a
Third Party designated by DSP; together with directly allocable manufacturing overheads specifically attributable to the Manufacture or
formulation of the Compound or Product under this Agreement, including depreciation and maintenance costs of fixed assets that are
wholly dedicated to and used in manufacturing the Compound or Product for DSP; but excluding corporate, general or administrative
overheads. Actual Costs shall be calculated in accordance with Intercept’s standard cost accounting policies and with generally accepted
accounting principles, consistently applied to the manufacture of pharmaceutical compounds and products.

“Additional Indications” shall have the meaning set forth in the second recital of this Agreement.

“Additional Indications Option” shall have the meaning set forth in Section 7.2.

“Additional Indications Option Commencement Notice” shall have the meaning set forth in Section 7.3.

“Additional Indications Exercise Period” shall have the meaning set forth in Section 7.3.

“Additional Indications Option Fee” shall have the meaning set forth in Section 7.3.

“Affiliate”  shall  mean  any  corporation,  firm,  limited  liability  company,  partnership  or  other  entity  that  directly  controls  or  is
controlled  by  or  is  under  common  control  with  a  Party  to  this  Agreement.  For  purposes  of  this  definition  only,  “control”  and,  with
correlative  meanings,  the  terms  “controlled  by”  and  “under  common  control  with”  shall  mean  the  possession,  directly  or  indirectly
through one or more intermediaries, of the power to direct the management or policies of an entity, whether through the ownership of
fifty percent (50%) or more of the voting securities of the other organization or entity or by contract relating to voting rights or corporate
governance. Notwithstanding the foregoing, Sumitomo Chemical Co., Ltd. (“Sumitomo Chemical”), the parent company of DSP, shall
not be considered an Affiliate for the purposes of this Agreement; provided that DSP shall be permitted to engage in routine reporting of
matters concerning this Agreement to Sumitomo Chemical.

“Clinical Supply Agreement” shall have the meaning set forth in Section 6.1.

“Clinical Supplies” shall mean Compound formulated into Product or matching placebos to be used exclusively for conducting

clinical studies to gain Regulatory Approval in the Territory.

“CMC” shall mean the Chemistry, Manufacturing and Controls information required to be submitted under Section 505 of the

U.S. Food, Drug and Cosmetic Act (as amended) and 21 C.F.R. 312.23(a)(7) and 314.50(d)(1).

2

“Commercial Supplies” shall mean the supply of the Product in bulk formulation (either packaged or pre-packaged) made to

DSP by Intercept pursuant to Section 6.2 of this Agreement and the Commercial Supply Agreement.

“Commercial Supply Agreement” shall have the meaning set forth in Section 6.2.

“Commercialize”  shall  mean  to  promote,  market,  distribute,  sell  (and  offer  for  sale  or  contract  to  sell)  or  provide  product
support for a Product, including by way of example: (i) detailing and other promotional activities in support of a Product; (ii) advertising
and  public  relations  in  support  of  a  Product,  including  market  research,  development  and  distribution  of  selling,  advertising  and
promotional materials, field literature, direct-to-consumer advertising campaigns, media/journal advertising, and exhibiting at seminars
and  conventions;  and  (iii)  developing  reimbursement  programs  and  information  and  data  specifically  intended  for  managed  care
organizations, governmental agencies and the like.

“Commercially  Reasonable  Efforts”  shall  mean  with  respect  to  a  Party’s  obligations  under  this  Agreement,  including  to
Develop,  Manufacture  or  Commercialize  the  Product,  those  efforts  and  resources  consistent  with  the  usual  practices  of  such  Party  in
pursuing  the  development  or  commercialization  of  its  own  pharmaceutical  products  that  are  of  similar  market  potential  and  strategic
value  as  such  Product,  taking  into  account  all  relevant  factors  including  product  labeling  or  anticipated  labeling,  present  and  future
market potential, past performance of such product and such Party’s other pharmaceutical products that are of similar market potential,
financial  return,  medical  and  clinical  considerations,  past  and  future  regulatory  environment  and  competitive  market  conditions,  all
measured  by  the  facts  and  circumstances  at  the  time  such  efforts  are  due.  Commercially  Reasonable  Efforts  shall  be  determined  on  a
country-by-country and indication-by-indication basis for the Product, and it is anticipated that the level of effort will change over time,
reflecting changes in the status of the Products and the market(s) or countries involved.

“Confidential Information” shall mean with respect to a Party (the “Receiving Party”), all information which is disclosed by
the other Party (the “Disclosing Party”) to the Receiving Party hereunder or to any of its employees, consultants, Affiliates, licensees or
sublicensees, which is marked as confidential or indicated at the time of disclosure as being confidential (and subsequently summarized
in writing) except to the extent that the Receiving Party can demonstrate by written record that such information, (i) as of the date of
disclosure is demonstrably known to the Receiving Party or its Affiliates other than by virtue of a prior confidential disclosure to such
Party or its Affiliates; (ii) as of the date of disclosure is in, or subsequently enters, the public domain, through no fault or omission of the
Receiving  Party;  (iii)  is  obtained  from  a  Third  Party  having  a  lawful  right  to  make  such  disclosure  free  from  any  obligation  of
confidentiality to the Disclosing Party; or (iv) is independently developed by or for the Receiving Party without reference to or reliance
upon any Confidential Information of the Disclosing Party; or (v) is required to be disclosed by judicial or governmental authority of
competent jurisdiction; provided that the Receiving Party shall first provide the Disclosing Party with sufficiently timely notice of such
requirement  to  permit  the  Disclosing  Party  to  take  measures  to  avoid  or  limit  the  scope  of  the  requested  disclosure.  Confidential
Information  shall  include,  without  limitation,  results  and  data  of  any  type  whatsoever,  in  any  tangible  or  intangible  form  whatsoever,
including,  preclinical  data,  clinical  trial  data,  databases,  practices,  methods,  techniques,  specifications,  formulations,  formulae,
knowledge,  know-how,  skill,  experience,  test  data  including  pharmacological,  biological,  chemical,  biochemical,  toxicological  and
clinical test data, analytical and quality control data, stability data, studies and procedures.

3

“Compound” shall have the meaning set forth in the first recital of this Agreement.

“Control” or “Controlled” shall mean, when used in reference to intellectual property, other intangible property, or materials,
that a Party owns or has a license or sublicense to such intellectual property, other intangible property or materials, and has the ability to
grant  a  license  or  sublicense  or  other  right  to  use  such  intellectual  property,  other  intangible  property  or  materials,  as  applicable,  as
provided for herein, without violating the terms of any agreement or other arrangement with any Third Party; provided that where the
ability to grant a license or sublicense is subject to a Third Party consent or notice requirement, “Commercially Reasonable Efforts” shall
require seeking such consent or providing such notice to the Third Party.

“Country Option” shall have the meaning set forth in Section 8.1.

“Country Option Exercise Notice” shall have the meaning set forth in Section 8.2.

“Development” and “Develop” shall mean with respect to the Compound or the Product, all activities relating to preparing and
conducting non-clinical studies, clinical studies (Phase I Clinical Trials, Phase II Clinical Trials, Phase III Clinical Trials and Phase IV
Clinical  Trials),  formulation,  development,  statistical  analysis,  quality  assurance  and  quality  control  activities  and  other  product
development activities, which may include, but is not limited to, research, and regulatory activities directed toward obtaining Regulatory
Approval of the Product in the Field inside or outside the Territory, as the case may be.

“DSP Defense Costs” shall have the meaning set forth in Section 12.3.

“Effective Date” shall have the meaning set forth in the first line of this Agreement.

“Eroded Country” shall have the meaning set forth in Section 9.3.1.

“Exclusive Period”  shall  mean,  on  a  country-by-country  basis,  the  period  beginning  upon  the  First  Commercial  Sale  of  the
Product in the relevant country until the later to occur of (i) the expiration of (x) the Intercept substance patent with respect to Japan or
(y) the last to expire of the Intercept patent family members with respect to China, after giving effect, in each of items (x) and (y) to any
Patent Term Extensions, and (ii) the date upon which generic drugs relying on the Compound or Product data for Regulatory Approval
may be introduced.

“Field” shall have the meaning set forth in the first recital of this Agreement, together with any other Additional Indications,

which shall each automatically be included in the “Field” upon the exercise by DSP of the Additional Indication Option.

4

“First Commercial Sale” shall mean, on a country-by-country basis, the date of the first arm’s length transaction, transfer or
disposition for value to a Third Party of a Product by or on behalf of DSP or any Affiliate or sublicensee of DSP in such country after
receipt of Marketing Approval, (and any labeling or pricing negotiations that may be required after Marketing Approval for such Product
in the Territory.) 
 A First Commercial Sale shall not include any Product sold for use in clinical trials, for research or for other non-
commercial uses, or that is supplied as part of a compassionate use or similar program.

“First Tier Royalty Rate” shall have the meaning set forth in Section 9.2.3.

“GMP” shall mean all applicable Good Manufacturing Practices standards, including, as applicable, those standards required by

the MHLW or its equivalent in each country in the Territory.

“Good  Clinical  Practices”  or  “GCP”  shall  mean  all  applicable  Good  Clinical  Practice  standards  for  the  design,  conduct,
performance,  monitoring,  auditing,  recording,  analyses  and  reporting  of  clinical  trials,  including,  as  applicable,  (i)  those  standards
required by the MHLW or its equivalent in the Territory, and (ii) the equivalent Laws in any relevant country, each as may be amended
and  applicable  from  time  to  time  and  in  each  case,  that  provide  for,  among  other  things,  assurance  that  the  clinical  data  and  reported
results are credible and accurate and protect the rights, integrity, and confidentiality of trial subjects.

“Good  Laboratory  Practices”  or  “GLP”  shall  mean  all  applicable  Good  Laboratory  Practice  standards,  including,  as
applicable, (i) those standards required by the MHLW as hereinafter defined or its equivalent in each country in the Territory, and (ii) the
equivalent Laws in any relevant country, each as may be amended and applicable from time to time.

“Improvement”  shall  mean  any  improvements,  enhancements  or  modifications  to  the  Intercept  Technology,  the  Intercept
Manufacturing Technology, or other technology claimed in the Intercept Patents (whether patentable or not), which would be useful or
necessary in the Manufacture, Development, and Commercialization of the Compound and/or Products, which is conceived, solely by
one Party or jointly by one Party with a Third Party or jointly by both Parties.

“IND” shall mean the equivalent application of an Investigational New Drug Application to the MHLW or its equivalent in any
country in the Territory, such as a clinical trial application or a clinical trial exemption, the filing of which is necessary to commence or
conduct clinical testing of a pharmaceutical product in humans in such country.

“Intercept  Change  of  Control”  shall  mean:  (i)  the  liquidation  or  dissolution  of  Intercept  or  the  sale  or  other  transfer  by
Intercept of all or substantially all of its respective assets; or (ii) the occurrence of a tender offer, stock purchase, other stock acquisition,
merger,  consolidation,  recapitalization,  reverse  split,  sale  or  transfer  of  assets  or  other  transaction,  as  a  result  of  which  any  person  or
entity (x) becomes the beneficial owner, directly or indirectly (including through multiple entities), of respective securities of Intercept
representing more than fifty percent (50%) of the combined voting power with respect to the election of directors of Intercept, (y) obtains
the ability to appoint a majority of the Board of Directors of Intercept, or (z) obtains the ability to direct the operations or management of
Intercept or any successor to the business of Intercept.

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“Intercept Development Plan” shall have the meaning set forth in Section 3.1.2.

“Intercept Know-How” shall mean the Know-How which Intercept or its Affiliates Control on the Effective Date or during the
Term,  which  information  is  necessary  or  useful  for  the  Development,  Manufacture  or  Commercialization  of  the  Product  or  the
Compound in the Field in the Territory.

“Intercept  Manufacturing  Know-How”  shall  mean  all  methods,  processes,  designs,  patterns,  or  know-how,  programs,
systems, procedures, technical data, technology, information, data, results of tests, studies, and analyses, whether patentable or not, which
are specifically related to the manufacturing process of the Compound and/or the Product, including Know-How that is in the case of
each of the foregoing Controlled by Intercept (or its Affiliates) as of the Effective Date or during the Term of this Agreement.

“Intercept Manufacturing Patent” shall mean any Patent that is Controlled by Intercept (or its Affiliates) as of the Effective
Date  and/or  during  the  Term,  in  each  case,  which  is  necessary  or  useful  for  the  Manufacture  of  the  Compound  or  the  Product  for
Commercialization in the Field in the Territory.

“Intercept Manufacturing Technology” shall mean the Intercept Manufacturing Know-How and the Intercept Manufacturing

Patents.

“Intercept Patents” shall mean all Patents that Intercept Controls as of the Effective Date or during the Term, which Patents
are necessary or useful for the purpose of Development, Manufacture or Commercialization of the Compound or the Product in the Field
in the Territory, all as more particularly set forth on Exhibit A.

“Intercept Technology”  shall mean the Intercept Patents and the Intercept Know-How.

“Joint Steering Committee” or “JSC” shall mean the joint steering committee formed by the Parties as described in Section

3.1.

“Joint  Improvements”  shall  mean  an  Improvement  or  invention,  whether  patentable  or  not,  which  is  invented,  made  or
discovered jointly by or on behalf of the employee(s), licensee(s) (including sublicensees), or contractors (including subcontractors) of
both Parties (and/or their Affiliates).

“Know-How”  shall  mean  intellectual  property  including  any  asset  that  comprises  any  of  the  following  items  and  has  a
substantial  value  independent  of  the  services  of  any  individual:  inventions,  formulae,  processes,  designs,  patterns,  or  know-how;
copyrights; trademarks, trade names, or brand names; franchises; methods, programs, systems, procedures, campaigns, surveys, studies,
forecasts, estimates, customer lists, or technical data; and other similar items (whether or not in documentary form and whether or not
patentable, copyrightable or otherwise protectable under applicable Laws).

6

“Laws” shall mean all applicable laws, statutes, rules, regulations, directives, decisions, ordinances, guidelines concerning the

Development, Manufacturing and Commercialization of the Compound or the Product in the Field in the Territory.

“Manufacturing”  shall  mean  all  activities  related  to  the  production,  manufacture,  testing,  processing,  filling,  finishing,
packaging,  labeling,  inspection,  receiving,  holding  and  shipping  of  the  Compound  and/or  the  Product,  the  Clinical  Supplies  or  the
Commercial  Supplies,  or  any  raw  materials  or  packaging  materials  with  respect  thereto,  or  any  intermediate  of  any  of  the  foregoing,
including  process  and  cost  optimization,  process  qualification  and  validation,  commercial  manufacture,  stability  and  release  testing,
quality assurance and quality control. For clarity, “Manufacture” has a correlative meaning.

“Marketing Approval” shall mean (i) for the United States, the approval of an NDA, and (ii) for jurisdictions in the Territory,
the approval from the relevant Regulatory Authority necessary to market and sell the Product in that country, including, where required,
pricing approvals.

“Market Share” shall have the meaning set forth in Section 9.3.1.

“MHLW” shall mean the Japanese Ministry of Health, Labor and Welfare, or a successor agency thereto.

“NASH” shall have the meaning set forth in the first recital of this Agreement.

“Necessary Third Party Patents” shall mean, on a country-by-country and indication-by-indication basis, the patents that are
owned  or  controlled  by  a  Third  Party,  which  do  not  infringe  the  Intercept  Technology,  but  are  necessary  for  the  Development,
Manufacturing or Commercialization of the Compound or the Product in the Field, as reasonably determined in accordance with Section
4.3.

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“Net Sales” shall mean the gross amounts invoiced by DSP and its Affiliates and sublicensees for sales or other dispositions of
the Product to Third Parties that are not Affiliates or sublicensees in the Field in the Territory, in bona fide, arms-length transactions less
the  following  items,  as  allocable  to  such  Products  (if  not  previously  deducted  from  the  amount  invoiced):  (i)  trade,  cash  or  quantity
discounts,  credits  or  allowances  actually  allowed  (provided  that  such  discounts  are  applied  in  a  normal  and  customary  manner  with
respect to other similarly situated products of the selling party, and not in a manner which is unreasonably disproportionate to one or
more Products when compared to other products of the selling party); (ii) charge back payments, administrative fees, price reductions,
rebates  allowed  or  granted,  or  other  forms  of  consideration  to  managed  care  organizations,  government  agencies  or  trade  customers,
including  wholesalers  and  chain  and  pharmacy  buying  groups  (provided  that  such  discounts  are  applied  in  a  normal  and  customary
manner with respect to other similarly situated products of the selling party, and not in a manner which is unreasonably disproportionate
to one or more Products when compared to other products of the selling party); (iii) credits actually allowed for claims, allowances for
damaged  goods,  retroactive  price  reductions  or  returned  goods;  (iv)  prepaid  freight,  postage,  shipping,  customs  duties  and  insurance
charges; and (v) sales taxes, value added taxes, duties and other governmental charges. Such amounts shall be determined in accordance
with Japanese GAAP, consistently applied, or GAAP in effect in a country in the Territory, as permitted by DSP. Any of the items set
forth above that would otherwise be deducted from the invoice price in the calculation of Net Sales but which are separately charged to
Third Parties shall not be deducted from the invoice price in the calculation of Net Sales. Further, in the case of any sale or other disposal
other than in an arm’s length transaction exclusively for cash, such as barter or counter-trade, of any Product, or part thereof, Net Sales
shall  be  determined  by  referencing  Net  Sales  at  which  substantially  similar  quantities  of  the  Product  are  sold  in  an  arm’s  length
transaction for cash. Finally, financial compensation, if any, received by DSP from a subsequent resale of the Product by a third party
reseller, if any, shall be included in the calculation of Net Sales.

“NDA”  shall  mean  a  new  drug  application  or  its  equivalent  filed  with  a  Regulatory  Authority  in  the  Territory  seeking

Regulatory Approval to Commercialize the Product in the Territory for a particular indication within the Field.

“Non-Territory Data” shall have the meaning set forth in Section 4.2.2.

“Patents” means any patents and patent applications and all substitutions, divisions, continuations, continuations-in-part, any
patent issued with respect to any such patent applications, any reissue, reexamination, utility models or designs, renewal, adjustment or
extension (including any supplementary protection certificate) of any such patent, and any confirmation patent or registration patent or
patent of addition based on any such patent, and all counterparts thereof in any country owned or Controlled by a Party on the Effective
Date and during the Term of this Agreement.

“Patent  Term  Extension”  means  any  term  extensions,  adjustments,  supplementary  protection  certificates,  regulatory

exclusivity and equivalents thereof offering Patent protection beyond the initial term with respect to any issued Patents.

“PBC” shall have the meaning set forth in the first recital of this Agreement.

“Phase  I  Clinical  Trial”  means  a  clinical  trial  in  humans,  the  principal  purpose  of  which  is  to  make  a  preliminary

determination of metabolism, pharmacokinetics, dose findings or preliminary safety in healthy individuals or patients in the Territory.

“Phase  II  Clinical  Trial”  means  a  clinical  trial  in  humans,  the  principal  purpose  of  which  is  to  make  a  preliminary
determination  that  a  given  product  is  safe  in  the  population  in  the  Territory  for  its  intended  use  and  to  obtain  information  about  such
product’s efficacy sufficient to permit the design of further clinical trials, or if no further trials are necessary, to enable an Regulatory
Approval.

8

“Phase III Clinical Trials” shall mean a clinical trial of a Product conducted in human patients with a defined dose or a set of
defined  doses  of  a  Product  designed  to  ascertain  efficacy  and  safety  of  such  Product  for  the  purpose  of  submitting  applications  for
Regulatory Approval to the competent Regulatory Authorities.

“Phase IV Clinical Trials” means post-marketing studies to delineate additional information about a pharmaceutical product’s
risks and benefits, and optimal use, commenced after receipt of Regulatory Approval for a Product in the indication for which such trial
was conducted.

“Product”  shall  mean  any  pharmaceutical  composition  or  formulation  that  contains  the  Compound,  whether  or  not  such
Product is used as a single agent or in combination with other therapeutically active components, as the term “Product” may be further
defined in each of the Clinical Supply Agreement and the Commercial Supply Agreement.

“Product Development Plan” shall have the meaning set forth in Section 3.1.1.

“Quality Assurance Agreement” shall have the meaning set forth in Section 6.3.5.

“Regulatory Approval” shall mean all necessary approvals (including INDs, NDAs, product approvals, import permits, and, in
each case any supplements and amendments thereto), licenses, registrations or authorizations of any Regulatory Authority, necessary for
the Development, Manufacture, and Commercialization of the Compound or the Product in the Field in the Territory.

“Regulatory Authority” shall mean, in a particular country in the Territory, any applicable governmental authority involved in

granting Regulatory Approval in the Territory, including the MHLW.

“Second Tier Royalty Rate” shall have the meaning set forth in Section 9.2.3.

“Specifications” shall  mean  those  tests,  methods  and  acceptance  criteria  for  the  Compound  and  the  Product  required  in  the

Territory as set forth the in the IND and NDA.

“Target Actual Cost” shall have the meaning set forth in Section 6.2.2.

“Target Country” shall have the meaning set forth in Section 8.3.

“Technical Transfer” shall have the meaning set forth in Section 6.4.1.

“Technology”  shall  mean  and  include  any  and  all  unpatented,  proprietary  ideas,  inventions,  discoveries,  Confidential
Information,  biologic  materials,  data,  results,  formulae,  designs,  specifications,  methods,  processes,  formulations,  techniques,  ideas,
know-how, technical information (including, without limitation, structural and functional information), process information, pre-clinical
information,  clinical  information,  regulatory  filings,  and  any  and  all  proprietary  biological,  chemical,  pharmacological,  toxicological,
pre-clinical, clinical, assay, control and manufacturing data and materials.

“Term” shall have the meaning set forth in Section 15.1.

9

“Territory”  shall  mean  Japan  and  China  (excluding  Taiwan),  and  such  other  countries  which  are  the  subject  of  the  Country
Option, each of which shall be automatically deemed included in the Territory upon the exercise of the Country Option by DSP for such
country.

“Third Party” shall mean any person or entity other than DSP or Intercept, and their respective Affiliates.

“Third Tier Royalty Rate” shall have the meaning set forth in Section 9.2.3.

“Third Party Offer Notice” shall have the meaning set forth in Section 9.3.

“Wholesale Acquisition Cost” or “WAC” shall mean the wholesaler acquisition cost for the Product in the U.S.

2.          GRANT OF RIGHTS

2.1           Exclusive License

2.1.1           Grant of Exclusive License. Intercept hereby grants to DSP an exclusive, royalty-bearing license,
including  the  right  to  grant  sublicenses  in  accordance  with  Section  2.1.2,  under  the  Intercept  Technology  to  research,  Develop,  have
Developed,  make,  have  made,  use,  sell,  offer  for  sale,  have  sold,  import,  have  imported,  export  and  have  exported,  register,  for  the
purpose of Commercializing the Product in the Territory, for any and all uses within the Field, subject to the terms and conditions of this
Agreement. For clarification, the Parties agree that DSP’s appointing a sublicensee to engage in the Manufacture of the Compound or the
Product  outside  the  Territory  for  the  Development  and  Commercialization  of  the  Product  inside  the  Territory  shall  not  be  deemed  a
breach of this Agreement.

2.1.2           Right to Sublicense. After Intercept’s receipt of the Upfront Fee set forth in Section 9.1, DSP
shall have the right to grant sublicenses to any Affiliate or Third Party to all or any portion of its rights under the license granted to DSP
pursuant  to  this  Section  2;  provided,  however,  that  (i)  Intercept  shall  be  notified  of  and  approve  the  sublicensing  arrangement,  such
approval not to be unreasonably withheld, (ii) each such sublicensee agrees to be bound by all applicable Sections of this Agreement, and
(iii) DSP shall provide Intercept with a summary of such sublicensing agreements, to include (a) the country in the Territory applicable to
such  sublicensee,  (b)  the  full  legal  name  of  the  sublicensee,  (c)  the  applicable  indications  in  the  Field,  (d)  the  term  and  termination
provisions of the sublicensing agreement, and (e) the standard of performance applicable to the sublicensee with respect to its obligations
under  the  sub-licensing  agreement.  Items  (a)-(e)  inclusive  of  item  (iii)  of  the  preceding  sentence  shall  be  set  forth  in  a  format
substantially similar to Exhibit B, which shall also be executed by the relevant sublicensee affirming its understanding of and willingness
to comply with Sections of this Agreement applicable to it.

Intercept Patent by DSP or its Affiliates shall constitute a material breach of this Agreement.

2.1.3                      Patent Challenge.  Any  challenge  to  the  validity,  scope  or  enforceability  of  any  claim  in  an

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2.2           Registration. Upon DSP’s request, but only after Intercept’s receipt of the Upfront Fee set forth in Section
9.1, Intercept shall use Commercially Reasonable Efforts, at DSP’s sole expense, to register a “Senyo-Jisshiken Tohroku” (i.e. registration
of the exclusive license with the Japanese Patent Office) for DSP (or the equivalent in any other country in the Territory) with respect to
the Intercept Technology and Intercept Patents, which registration shall be transferred or assigned to DSP by Intercept immediately upon
issuance for no additional consideration.

2.3           No Implied Licenses; Retained Rights. Except as explicitly set forth in this Agreement, neither Party grants

any license, express or implied, under its intellectual property rights to the other Party, whether by implication, estoppel or otherwise

2.4           Bankruptcy-Related Rights.

2.4.1           U.S. Bankruptcy Code 365(n). All rights and licenses granted under this Agreement are hereby
deemed to be, for purposes of Section 365(n) of the U.S. Bankruptcy Code, licenses of rights to “intellectual property” as defined under
Section 101(35A) of the U.S. Bankruptcy Code. The Parties shall retain and may fully exercise all of their respective rights and elections
under the U.S. Bankruptcy Code. The Parties agree that DSP, as the licensee under this Agreement, shall retain and may fully exercise all
of  its  rights  and  elections  under  the  U.S.  Bankruptcy  Code,  and  that  upon  commencement  of  a  bankruptcy  proceeding  by  or  against
Intercept under the U.S. Bankruptcy Code, DSP shall be entitled to a complete duplicate of or complete access to any such intellectual
property and all embodiments of such intellectual property, provided that DSP continues to fulfill its payment or royalty obligations in
accordance with this Agreement. Such intellectual property and all embodiments thereof shall be promptly delivered to DSP (x) upon
any  such  commencement  of  a  bankruptcy  proceeding  upon  written  request  therefore  by  DSP,  unless  Intercept  elects  to  continue  to
perform all of its obligations under this Agreement or (y) if not delivered under (x) above, upon the rejection of this Agreement by or on
behalf  of  Intercept  upon  written  request  therefor  by  DSP.  The  foregoing  is  without  prejudice  to  any  rights  DSP  may  have  against
Intercept arising under the U.S. Bankruptcy Code or other applicable law.

2.4.2           Intellectual Embodiments. Each Party hereby acknowledges that (i) copies of research data (both
clinical and non-clinical), (ii) laboratory samples, (iii) product samples and inventory, (iv) formulae, (v) laboratory notes and notebooks,
(vi) data and results related to clinical and non-clinical trials, (vii) regulatory filings and approvals, (viii) rights of reference in respect of
regulatory  filings  and  approvals,  (ix)  pre-clinical  research  data  and  results,  and  (x)  marketing,  advertising  and  promotional  materials,
constitute “embodiments” of intellectual property pursuant to Section 365(n) of the Bankruptcy Code.

2.5           Bankruptcy Assistance.  Each  Party  agrees  not  to  interfere  with  the  other  Party’s  exercise  of  rights  and
licenses  to  intellectual  property  licenses  granted  to  the  Party  pursuant  to  Section  2.4  or  under  Section  365(n)  of  the  U.S.  Bankruptcy
Code and embodiments thereof in accordance with this Agreement and agrees to use Commercially Reasonable Efforts to assist the other
Party to obtain such intellectual property and embodiments thereof in the possession or control of Third Parties, as reasonably necessary
for the other Party to exercise such rights and licenses in accordance with this Agreement.

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3.          GOVERNANCE

3.1           Joint Steering Committee. The Parties shall use Commercially Reasonable Efforts to establish the JSC
within sixty (60) days after the Effective Date. The JSC shall engage in consultation, discussion and decision-making with respect to the
following:

Development Plan”) and any material amendments thereto;

3.1.1                      A  development  plan  for  the  Development  of  the  Product  in  the  Territory  (the  “Product

Intercept and/or its licensees outside the Territory(the “Intercept Development Plan”), and any material amendments thereto;

3.1.2                      A  development  plan  for  the  Development  of  the  Product  and  the  Additional  Indications  by

3.1.3           Clinical trials to be conducted in connection with the Development of the Compound and the
Product in the Field in the Territory; including, as appropriate Phase I Clinical Trials, Phase II Clinical Trials, Phase III Clinical Trials
and Phase IV Clinical Trials, including review of synopses of clinical study protocols;

Development of the Compound and the Product in the Field in the Territory;

3.1.4           Nonclinical studies, including CMC and formulations, to be conducted in connection with the

its licensees in connection with the Additional Indications Option;

3.1.5           Development of Additional Indications to be conducted outside the Territory by Intercept and/or

3.1.6           Matters related to Regulatory Approvals for Product in the Field in the Territory, including the
formulation of a plan consistent with this Agreement for the exchange of and reporting to Regulatory Authorities of safety data reported
or arising in the course of the Development;

3.1.7           The activities of any sub-committees;

3.1.8                      Encouraging  and  facilitating  communication  between  the  Parties  regarding  the  progress  and
results (whether preliminary or final) of the Development and Manufacturing activities for the Compound and the Product in the Field in
the Territory, including the coordination of clinical and nonclinical data exchange and preparation of regulatory filings;

Manufacturing Patents) and any patents issued on Improvements or Joint Improvements, and all Patent Term Extensions;

3.1.9           The filing, maintenance, and abandonment, if any, of the Intercept Patents (including the Intercept

including the details and timing of the Technical Transfer;

3.1.10                  Matters  relating  to  the  Manufacture  of  the  Clinical  Supplies  and  the  Commercial  Supplies,

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3.1.11         Establish internal rules for the governance and operation of the JSC; and

mutually agreed upon by the Parties in writing from time to time.

3.1.12         Such other responsibilities as may be assigned to the JSC pursuant to this Agreement or as may be

3.2                      JSC Membership.  The  initial  membership  of  the  JSC  shall  be  comprised  of  three  (3)  representatives
designated  by  each  of  DSP  and  Intercept,  at  least  one(1)  of  whom  from  each  Party  shall  be  senior  enough  within  its  respective
organization to have the requisite decision-making authority with respect to the matters set forth in Section 3.1 above, and all of whom
shall  have  appropriate  expertise  and  ongoing  familiarity  with  the  Development  and  Manufacturing  of  the  Product  in  the  Field  in  the
Territory. From time to time, the number and qualifications of the designated members to the JSC may be changed by the mutual written
agreement of the Parties, so long as an equal number of members from each of DSP and Intercept is maintained. Each Party shall inform
the other Party of its initial representatives to the JSC as soon as practicable after the Effective Date. Each Party may also designate non-
voting representatives to attend the meetings from time to time as necessity requires, but only with the consent of the other Party. The
JSC shall be chaired by a representative from DSP, who shall be responsible for (i) calling meetings, (ii) preparing and issuing minutes of
each  such  meeting  as  soon  as  practicable  following  each  meeting,  and  (iii)  preparing  and  circulating  an  agenda  for  the  upcoming
meeting, which shall include agenda items proposed by either Party no less than ten (10) calendar days prior to the next scheduled JSC
meeting.

3.3           JSC Meetings. The JSC shall hold meetings at least once every six months, and more frequently as necessity
requires. The first JSC meeting shall be held at a mutually agreed venue and date following the Effective Date. Meetings of the JSC shall
be effective only if at least one (1) representative of each Party is present or participating. The JSC may meet either (i) in person at either
Party’s  facilities,  or  (ii)  by  audio  or  video  teleconference.  Additional  meetings  of  the  JSC  may  also  be  held  with  the  consent  of  each
Party. Each Party shall be responsible for all of its own expenses incurred in connection with participating in the JSC meetings or any of
the other committee meetings.

3.4           Decision-Making. The JSC shall endeavor to reach consensus on all matters brought before it pursuant to
Section 3.1, with each Party having a single vote, irrespective of the number of representatives actually in attendance at a meeting. The
JSC shall use Commercially Reasonable Efforts to resolve the matters brought before it pursuant to Section 3.1. DSP shall have the final
decision making authority with respect to Development of the Compound and Product in the Field in the Territory. In the event that either
Party has concern about whether the Development and the Commercialization of the Compound and/or the Product is reasonably likely
to have a materially negative impact on the Compound or the Product inside or outside the Territory, the Parties shall consult through the
JSC for a period of thirty (30) days; failing resolution of which, such matter shall be elevated to the CEO of Intercept and the CEO of
DSP, for attempted resolution in good faith within the time frame set forth in Section 16.1.

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3.5           Progress Reports and Exhibit Amendments. At each meeting of the JSC and, as applicable, that of any
sub-committee or new committee established by the JSC, DSP shall provide Intercept with a written report summarizing its activities and
progress  regarding  the  Development  and  Commercialization  of  the  Compound  and  Product  in  the  Field  in  the  Territory,  including  its
marketing and promotional materials, which may, in DSP’s option, be in the local language of the country in the Territory to which it
pertains. At each meeting of the JSC, and, as applicable, that of any sub-committee or new committee established by the JSC, Intercept
shall provide DSP with a written report summarizing its Development activities of the Compound and Product outside the Territory and
its Development activities of the Additional Indications outside the Territory. In addition, at each meeting of the JSC, each Party shall
inform  the  other  of  any  Improvements  conceived  by  or  on  behalf  of  such  Party,  as  well  as  any  Joint  Improvements.  Notwithstanding
Section 17.4, upon the notification to the JSC through a progress report (or otherwise) of the filing of a patent application with respect to
any Improvement or Joint Improvement, Exhibit A shall be deemed automatically amended, and an updated version of Exhibit A shall be
distributed to the Parties together with the meeting minutes.

3.6           Sub-committees. From time to time, the JSC may establish and delegate duties to sub-committees to oversee
particular  projects  or  activities.  Each  such  sub-committee  shall  be  constituted  and  shall  operate  as  the  JSC  determines.  Each  sub-
committee and its activities shall be subject to the oversight, review and approval of, and shall report to, the JSC. It is contemplated that,
at the appropriate time, the JSC will expand its scope of activity to include consultation, discussion and decision-making with respect to
Commercialization  or,  alternatively,  decide 
to  govern
Commercialization planning and implementation. In the case that the JSC decides that such a new committee should be established, such
committee shall be formed and governed according to the same principles as the JSC.

that  a  separate  decision-making  committee  should  be  established 

3.7           Alliance Manager. Each Party shall designate an alliance manager, who shall be responsible for the day-to-
day coordination of the collaboration between the Parties and shall facilitate communication between the Parties. The Alliance Manager,
may but need not be, one of the designated members of the JSC.

4.          DEVELOPMENT AND COMMERCIALIZATION

4.1           Commercially Reasonable Efforts.

4.1.1           DSP’s Commercially Reasonable Efforts. From and after the Effective Date, DSP shall use
Commercially Reasonable Efforts to Develop and Commercialize the Compound and the Product in the Field (including with respect to
any Additional Indications) in the Territory. Subject to Section 9.4, DSP shall be responsible for all costs and expenses incurred by it in
connection with such Development and Commercialization activities.

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4.1.2           Intercept’s Commercially Reasonable Efforts. From and after the Effective Date, Intercept shall
use Commercially Reasonable Efforts to Develop the Compound and the Product anywhere outside the Territory, either on its own or
through  Third  Party  licensees  or  subcontractors.  In  addition,  from  and  after  the  Effective  Date,  Intercept  shall  (i)  use  Commercially
Reasonable  Efforts  to  Develop  the  Additional  Indications  outside  the  Territory  in  accordance  with  the  Intercept  Development  Plan
outside the Territory and (ii) shall use

Commercially  Reasonable  Efforts  to  cause  each  of  its  licensees  to  use  Commercially  Reasonable  Efforts  to  Develop  the  Additional
Indications outside the Territory.

4.2           Information and Data Exchange.

4.2.1           Intercept Technology. No later than thirty (30) days following Intercept’s receipt of the Upfront
Fee set forth in Section 9.1, Intercept shall transfer and otherwise make available to DSP, its Affiliates and its designated Third Party
subcontractors  the  Intercept  Technology  and  all  material  information  and  data  relating  thereto  to  enable  DSP  to  engage  in  the
Development and Commercialization of the Product in the Field in the Territory. The transfer of the Intercept Technology and related
information and data shall be made in readily accessible electronic format wherever possible. Following the payment of the “Upfront
Payment” pursuant to Section 9.1, Intercept shall, for no additional consideration, undertake to provide reasonable assistance DSP, its
Affiliates and sublicensees.

4.2.2                      Non-Territory  Data.  Intercept  shall  make  available  to  DSP,  its  Affiliates  and  Third  Party
subcontractors  any  clinical  and  non-clinical  data,  post-marketing  data  and  information  which  is  generated  by  or  in  connection  with
Intercept  and  its  licensees’  Development  of  the  Compound  and  Product,  both  in  the  Field  and  with  respect  to  Additional  Indications
outside  the  Territory  (the  “Non-Territory  Data”),  which  data  and  information  may  be  used  by  DSP  for  [***]  in  connection  with  its
Development, Commercialization and/or Manufacturing, as well as its activities to gain Regulatory Approval for the Product in the Field
in  the  Territory.  Intercept  shall  maintain  Non  -Territory  Data  in  conformity  with  all  applicable  Laws  and  regulations  and  in  a  good
scientific manner appropriate for patent and regulatory purposes. Intercept shall use Commercially Reasonable Efforts to cause any Third
Party or Affiliate who is engaged in the Development of the Compound or Additional Indications outside the Territory to provide access
to DSP and its Affiliates for the Non-Territory Data for [***].

4.3                      Necessary  Third  Party  Patents.  In  the  event  that  DSP  determines,  in  the  exercise  of  sound  business
judgment,  it  is  necessary  to  license  or  acquire  Necessary  Third  Party  Patents  in  connection  with  the  Development,  Manufacture  or
Commercialization  of  the  Product  in  the  Field  in  the  Territory,  it  shall  so  notify  Intercept  in  writing  explaining  the  reasons  therefor,
following  which  the  Parties  shall  engage  in  good  faith  discussions  concerning  such  matter.  DSP’s  request  for  Necessary  Third  Party
Patents shall require Intercept’s prior consent, which shall not be unreasonably withheld or delayed.

4.4           Records. DSP shall maintain scientific records, in sufficient detail and in good scientific manner appropriate
for patent and regulatory purposes, which will fully and properly reflect all work done and results achieved in the performance of the
Development and Commercialization activities with respect to the Product in the Field in the Territory; all of the foregoing in conformity
with  standard  pharmaceutical  industry  practices,  the  terms  and  conditions  of  this  Agreement,  and  all  applicable  Laws  and  regulations
(including re-examination systems for post-marketing information). DSP shall provide Intercept with reasonable access to the scientific
records maintained by DSP pursuant to this Section 4.4 which may be used by Intercept in pursuance of its Development activities for
the Compound and the Product outside the Territory.

15

4.5           Cooperation. Except as expressly forth herein, each Party shall, at its own cost and expense, provide all
reasonable  assistance  and  take  all  actions  reasonably  requested  by  the  other  Party  that  are  necessary  or  desirable  to  enable  the
Development and Commercialization of the Product in the Field in the Territory. Further, Intercept shall provide reasonable assistance to
DSP to prepare the regulatory materials for Regulatory Approval and to respond to Regulatory Authorities’ inquiries and investigation
relating to analysis of data arising from non-clinical studies, pre-clinical studies and/or clinical trials conducted by Intercept. In the event
that  a  Regulatory  Authority  and/or  DSP  reasonably  requests  Intercept  to  disclose  its  data  and  documentation  related  to  the  Intercept
Technology for an IND or NDA to be prepared or filed outside the Territory, Intercept shall cooperate with this request by providing such
Regulatory Authority and DSP with the requested data and documentation. In the event that DSP reasonably requests to audit Intercept
and  its  sub-contractors  or  licensees,  Intercept  shall,  and  shall  cause  its  licensees  and  sub-contractors  to,  allow  such  audit,  subject  to
customary prior notice requirements.

5.          REGULATORY MATTERS

5.1           Commercially Reasonable Efforts. DSP shall use Commercially Reasonable Efforts, at its own expense,
with respect to all regulatory activities concerning the Development and Commercialization of the Products in the Field in the Territory.
DSP shall have sole responsibility for all pricing and reimbursement approval proceedings relating to each Product in the Field in the
Territory. In the event that DSP wishes to commence Development of the Product in China following Intercept’s receiving Regulatory
Approval in the U.S. and prior to the receipt of Regulatory Approval in Japan, Intercept shall cooperate with DSP based on mutual good
faith discussions. Upon reasonable prior notice and during normal business hours, Intercept shall, and shall cause its Affiliates and its
Third Party sub-contractors to whom all or a part of the Development outside the Territory has been entrusted or contracted, to allow the
inspection  by  a  Regulatory  Authority  which  is  required  as  a  condition  of  Regulatory  Approval  for  the  Product  in  the  Field  in  the
Territory. DSP shall use its Commercially Reasonable Efforts to provide any information concerning such inspection to Intercept in a
timely manner. Intercept shall manage, but shall permit DSP or its designated representatives to be present at any inspection conducted
by  such  Regulatory  Authority.  If  any  issue  or  concerns  are  raised  concerning  the  Development  of  the  Compound  or  the  Product  in
connection with the inspection by such Regulatory Authority, Intercept shall immediately inform and discuss with DSP to solve the issue,
including any recommendations made by the Regulatory Authority.

5.2           Ownership of Regulatory Approvals. DSP (or its designated Affiliate or sublicensee) shall be the holder of
all  Regulatory  Approvals  issued  by  Regulatory  Authorities  with  respect  to  the  Product  in  the  Field  in  the  Territory  and  shall  be
responsible, at its own cost, for preparing and, subject to Section 5.1 hereof, drafting all regulatory filings in the Territory (including any
supplements or modifications thereto). DSP (or through its designated Affiliate or sublicensee) shall, subject to Section 5.1 above, be
responsible for communicating with and negotiating with all Regulatory Authorities in the Territory and shall keep Intercept informed of
the status of regulatory filings.

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5.3           Pharmacovigilance. The Parties agree to handle safety information including adverse events occurring or
having occurred in connection with the use of the Compound or the Product in accordance with applicable Laws and requirements of
relevant Regulatory Authorities. The Parties shall exchange all safety information including adverse events occurring or having occurred
in connection with the use of the Compound or the Product. The Parties shall execute a separate agreement relating to safety matters on
the Compound or the Product including the procedure for the exchange of safety information during the Term of the Agreement.

6.          MANUFACTURING

6.1           Clinical Supply. Intercept shall, by itself or through its Third Party contract manufacturers, supply to DSP
(or its Affiliates, sublicensees or sub-contractors) all quantities of Clinical Supplies of the Product (packaged or prepackaged) required
by DSP to Develop the Product in the Field in the Territory and for quality control analysis. The Parties shall discuss in good faith and
cooperate  with  each  other  with  respect  to  the  negotiation  of  a  manufacturing  and  clinical  supply  agreement  (the  “Clinical  Supply
Agreement”)  governing  the  supply  of  Clinical  Supplies  of  the  Product  (packaged  or  pre-packaged).  Intercept  undertakes  to  improve
quality  assurance  system  and  /or  organization  to  supply  DSP  (or  its  Affiliates,  sublicensees  or  sub-contractors)  with  Clinical  Supply,
including permitting and causing any of its Third Party sub-contractors to permit, an audit by DSP for quality assurance purposes. The
Clinical Supply Agreement shall include, among other customary provisions, the following or substantially equivalent provisions:

6.1.1           Intercept shall, before entering into any negotiations for an agreement with a Third Party contract
manufacturer of Clinical Supplies for supply to DSP (or its Affiliates, sublicensees or sub-contractors) hereunder notify DSP of the fact.
Thereafter,  DSP  shall  have  the  right  to  provide  input  within  thirty  (30)  days  regarding  the  terms  of  such  agreement  (as  well  as  any
amendments  thereof),  review  and  comment  on  the  draft  agreement  and  participate  in  person  in  the  negotiation  of  such  agreement.
However,  Intercept  shall  have  final  determination  of  the  terms. Further,  Intercept  shall  provide  DSP  with  an  execution  copy  of  each
agreement between Intercept and any Third Party contract manufacturer.

17

6.1.2                      From  time  to  time,  DSP  shall  submit  to  Intercept  purchase  orders  for  quantities  of  Clinical
Supplies  and  Intercept  shall  supply  or  have  supplied  to  DSP  such  quantities  of  Clinical  Supplies.  DSP’s  sole  financial  liability  with
respect to Clinical Supplies shall be to reimburse Intercept for the Actual Costs. DSP shall provide Intercept with non-binding forecasts
of  DSP’s  purchase  orders  for  Clinical  Supplies  which  may  be  placed  for  the  initial  [***]  ([***])  [***]  after  the  Effective  Date,  and
thereafter DSP shall provide Intercept with non-binding forecasts of DSP’s purchase order for Clinical Supplies [***] ([***]) [***] prior
to the estimated date of placing the purchase order. The purchase orders for Clinical Supplies shall be placed to allow no less than [***]
([***]) [***] lead time prior to the shipment dates specified in the purchase orders, and upon placement shall be deemed non-cancelable,
unless  Intercept  indicates  that  it  does  not  have  sufficient  stock  of  Clinical  Supplies  to  accommodate  the  lead  time  specified  in  DSP’s
purchase  order,  in  which  event  the  lead  time  for  the  Clinical  Supplies  for  such  order  shall  be  determined  by  mutual  agreement  of
Intercept and DSP through good faith discussions; provided that should the Parties not reach agreement on an adjusted lead time, then
DSP may cancel the relevant purchase order. Notwithstanding the foregoing, Intercept shall use best reasonable efforts to comply with
the  purchase  orders.  The  risk  of  loss  and  damage  for,  and  the  title  in,  Clinical  Supplies  supplied  hereunder  shall  pass  to  DSP  upon
delivery of the Clinical Supplies to the carrier designated by DSP. Shipment shall be FCA an international airport or port designated by
Intercept as defined in INCOTERMS 2010, as amended. DSP may at any time elect to Manufacture or have Manufactured the Clinical
Supplies,  provided  such  election  will  not  terminate  any  purchase  orders  for  Clinical  Supplies  submitted  by  DSP  to  Intercept  prior  to
notice of such election.

6.1.3           Intercept shall invoice DSP for such Clinical Supplies with each shipment, clearly setting forth the
calculation of the Actual Cost for the shipped order of the Clinical Supplies and DSP shall pay such invoices within thirty (30) days of its
receipt of such invoice.

6.2           Commercial Supply. Intercept shall supply DSP (or its Affiliates, sublicensees or sub-contractors) with all
DSP’s  requirements  of  the  Commercial  Supplies  until  such  time  as  DSP  provides  written  notice  to  Intercept  that  DSP  is  ready  to
commence  Manufacturing  (or  have  Manufactured)  of  the  Product  on  its  own  or  on  its  behalf.  Intercept  shall  be  responsible  for  the
Manufacture of the Commercial Supplies in compliance with the Specifications, GMP and all applicable Laws. The Parties shall discuss
in  good  faith  and  cooperate  with  respect  to  the  negotiation  of  a  manufacturing  and  supply  agreement  (the  “Commercial  Supply
Agreement”) governing the supply of the Commercial Supply by or on behalf of Intercept, to DSP (or its Affiliates, sublicensees or sub-
contractors) for the Commercialization of the Product in the Field in the Territory at the initiation of the Phase III Clinical Trials in Japan.
In  the  event  that  manufacturing  batches  for  the  U.S.  are  conducted  prior  to  the  commencement  of  Phase  III  Clinical  Trials  in  Japan,
Intercept  shall  afford  DSP  a  reasonable  opportunity  to  comment  upon  and  make  suggestions  with  respect  to  such  manufacturing
validation, which Intercept shall use good faith efforts to incorporate on a going-forward basis. The Commercial Supply Agreement shall
contain, in addition to other customary terms, the following terms and conditions:

6.2.1           The transfer price for the first three orders of the Commercial Supply supplied to DSP by or on
behalf of Intercept following receipt of Marketing Approval in Japan shall be calculated at the rate of [***] percent ([***]%) of [***] in
effect on the date upon which each such order is sent to Intercept by DSP.

6.2.2           The fourth and subsequent orders of the Commercial Supply supplied to DSP by or on behalf of
Intercept following receipt of Marketing Approval in Japan shall be based on the Actual Cost plus [***] percent ([***]%) of the Actual
Costs. The target actual cost is less than or equal to $[***] (the “Target Actual Cost”). In the event that the Actual Cost exceeds such
Target  Actual  Cost,  Intercept  shall  use  Commercially  Reasonable  Efforts  to  reduce  the  Actual  Cost.  Should  that  not  be  possible,  the
Parties shall discuss in good faith an increased Target Actual Cost for the Product.

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6.2.3           Intercept shall, before entering into any negotiation for an agreement with a Third Party contract
manufacturer of Commercial Supplies to DSP hereunder, notify DSP of the fact. Thereafter, DSP shall have the right to provide input
regarding the terms of such agreement (as well as any amendments thereof), review and comment on the draft agreement and participate
in person in the negotiation of such agreement. Further, Intercept shall provide DSP with an execution copy of each agreement between
Intercept and any Third Party contract manufacturer.

6.3                      Additional  Supply  Terms  and  Conditions.  In  addition  to  the  supply  terms  and  conditions  to  be
incorporated  in  the  Clinical  Supply  Agreement  and  the  Commercial  Supply  Agreement  pursuant  to  Sections  6.1  and  6.2  respectively,
each of the Clinical Supply Agreement and the Commercial Supply Agreement shall also include provisions substantially similar to the
following:

the Clinical Supply and the Commercial Supply Agreement shall strictly conform to (i) the Specifications and (ii) GMP.

6.3.1           Conformity. All Products Manufactured and supplied by or on behalf of Intercept under each of

6.3.2                      Change  Control.  If  Intercept  wishes  to  change  the  Specifications,  the  location  of  the
Manufacturing site, the Manufacturing process, or the raw materials, which in the case of each of the foregoing requires approval of the
Regulatory Authorities, Intercept shall first obtain the prior written consent of DSP (not to be unreasonably withheld) and provide the
information relevant to such proposed change to DSP, following which DSP shall use Commercially Reasonable Efforts to obtain any
required  approval  from  the  Regulatory  Authorities.  Intercept  shall  provide  DSP  with  all  reasonable  assistance  with  respect  to  the
foregoing. When Intercept wishes to make any change in the Manufacturing process or the raw materials which, in either case, is subject
to a reporting or notification requirement to Regulatory Authorities, Intercept shall notify DSP sufficiently in advance so that DSP may
comply  with  such  reporting  or  notification  requirements.  Prior  to  initiating  any  change  in  the  Specifications,  the  location  of  the
Manufacturing site, the Manufacturing process, or the raw materials, Intercept and DSP shall discuss in good faith and agree upon the
quantity of a reasonable safety stock of the Product to be maintained until completion of the any proposed change.

6.3.3           GMP Audit by DSP. DSP may audit the facilities of Intercept, its Affiliates or its Third Party
subcontractors upon reasonable prior notice and during normal business hours. Intercept shall allow and shall cause its Affiliate or its
Third Party subcontractors to allow such inspection to the extent such facilities relate to the Manufacture of the Compound and/or the
Product.  Intercept  shall,  and  shall  cause  its  Affiliates  and  Third  Party  sub-contractors,  to  use  Commercially  Reasonable  Efforts  to
implement changes reasonably requested by DSP as a result of any GMP audit undertaken pursuant to the preceding sentence.

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6.3.4           Inspection by Regulatory Authority. Upon reasonable prior notice and during normal business
hours, Intercept shall allow, and shall cause its Affiliates and its Third Party subcontractors to whom all or a part of the Manufacturing
process of the Compound and/or the Product has been entrusted or contracted to allow, the inspection by the Regulatory Authority which
is required as a condition for obtaining or maintaining Regulatory Approval for the Product in the Field in the Territory. DSP shall use its
Commercially  Reasonable  Efforts  to  provide  any  information  concerning  such  audit  to  Intercept  in  a  timely  manner.  Intercept  shall
permit DSP or its designated representatives to be present at any audit conducted by any Regulatory Authority pursuant to this Section
6.3.4. If any issue or concerns are raised concerning the Manufacturing of the Compound or Product in connection with the audit by such
Regulatory Authority, Intercept shall immediately inform DSP, including any recommendations made by the Regulatory Authority.

6.3.5           Quality Assurance Agreement. The Parties shall enter into a mutually agreed-upon companion
quality  agreement  (the  “Quality  Assurance  Agreement”)  with  respect  to  each  of  the  Clinical  Supply  Agreement  and  the  Commercial
Supply  Agreement,  which  shall  set  forth  in  detail  the  quality  assurance  arrangements  and  procedures  of  the  Product  and  the  GMP
responsibilities between the Parties prior to the Manufacture of the Compound to be used for the first commercial lot of the Product.

6.4           Technical Transfer. In the event that DSP wishes to commence the Manufacture of the Compound and/or
Product  itself  (including  having  the  Product  Manufactured),  DSP  shall  raise  the  issue  to  the  JSC  for  consultation  with  Intercept  with
respect to the timing and other related details of the Technical Transfer of the Intercept Manufacturing Technology so to enable DSP to
Manufacture or have Manufactured the Compound and the Product for Commercialization in the Territory.

6.4.1           Immediate Transfer. Following  consultation  with  the  JSC,  Intercept  shall  use  Commercially
Reasonable Efforts to make available, or cause to be made available, in either case, within sixty (60) days to DSP, its Affiliates, and its
designated Third Party subcontractors, all relevant information, data, and Intercept Know-How relating to the Intercept Manufacturing
Technology. To give effect to the foregoing, DSP shall have the right to obtain transfer and Intercept shall have the obligation to give
immediate transfer free of charge to DSP, its Affiliates and its designated Third Party subcontractors, without undue delay, of any and all
Intercept Manufacturing Technology necessary to enable DSP to Manufacture or have Manufactured the Compound and/or Product by a
Third Party subcontractor to meet DSP’s requirements (the foregoing, the “Technical Transfer”).

6.4.2           Additional Licenses. In connection with the Technical Transfer, Intercept hereby grants to DSP a
non-exclusive right, non-royalty-bearing license, with the right to sublicense to its Affiliates and Third Party subcontractors, with prior
notice  to  and  reasonable  approval  of  Intercept,  to  use  the  Intercept  Manufacturing  Technology  both  in  the  Territory  and  outside  the
Territory  to  engage  in  the  Manufacture  of  the  Compound  and/or  Product  for  Commercialization  in  the  Territory.  If  any  Intercept
Manufacturing Technology is within the control or possession of a Third Party, Intercept shall use Commercially Reasonable Efforts to
obtain the cooperation and assistance of such Third Party in connection with the Technical Transfer.

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6.4.3           Assistance and Continued Supply Obligation. Both Parties acknowledge that the process of
DSP’s becoming manufacturing-ready may require reasonable assistance from Intercept, which Intercept agrees to provide as reasonably
requested.  At  the  request  of  DSP  made  pursuant  to  Section  6.4,  Intercept  shall  facilitate  the  transfer  of  the  Intercept  Manufacturing
Technology  from  Intercept’s  contract  manufacturers  to  DSP  and/or  its  contract  manufacturers,  in  which  case  the  expenses  reasonably
incurred for the Technical Transfer shall be borne by DSP. During the Term of this Agreement, Intercept shall remain available to answer
technology  transfer  questions  relating  to  the  Intercept  Manufacturing  Technology.  In  the  event  DSP  should  require  any  additional
technical assistance beyond the Term of this Agreement, Intercept shall provide such assistance at DSP’s expense to the extent Intercept
has  personnel  available.  Intercept  makes  no  warranty,  express  or  implied,  with  respect  to  the  Intercept  technical  assistance.  Further,
Intercept  shall  supply  the  Clinical  Supplies  and  Commercial  Supplies  to  DSP  hereunder  until  DSP  indicates  that  it  is  ready  to
Manufacture  or  have  Manufactured  the  Compound  or  Product.  If,  notwithstanding  Intercept’s  Commercially  Reasonable  Efforts,
Intercept  reasonably  determines  that  Manufacture  and  supply  of  the  Commercial  Supply  are  not  practicable  for  a  technical  and/or
economic reason, Intercept’s commitment to supply Product may be terminated upon three (3) years prior written notice to DSP, in which
event Intercept shall, (i) at DSP’s option, (x) assign to DSP certain contracts between Intercept and its subcontractors which are selected
by DSP or (y) arrange for DSP to negotiate its own terms and conditions with Intercept’s subcontractors designated by DSP, and (ii) bear
all reasonable cost and effects arising in connection with the Technical Transfer.

7.          ADDITIONAL INDICATIONS OPTION

7.1                      Development  of  Additional  Indications  for  Products.  The  Parties  shall  cooperate  in  good  faith  in

generating ideas and concepts for Additional Indications for Products.

7.2           Grant of Option. Subject to the terms and conditions of this Agreement and throughout the Term of the
Agreement, Intercept hereby grants to DSP the exclusive option to an exclusive license to Products in the Territory for each and every
Additional  Indication  (both  present  and  future)  on  the  same  terms  and  conditions  as  provided  for  the  Product  in  the  Field  (each  such
Additional Indication, an “Additional Indication Option”). For the avoidance of doubt, the rights granted to Intercept pursuant to Section
7.3.3  below  with  respect  to  Third  Parties  shall  have  effect  only  in  the  event  that  DSP  declines  to  exercise  a  particular  Additional
Indications Option.

7.3           Exercise Period; Exercise of Additional Indications Option. The period during which DSP may exercise
each Additional Indications Option shall commence on the date that Intercept notifies DSP in writing of the “first patient” in a Phase III
Clinical  Trial  for  the  target  Additional  Indication  by  Intercept  and/or  its  licensees  outside  the  Territory  (the  “Additional  Indications
Option Commencement Notice”) and shall end on the [***] ([***]) [***] of the receipt by DSP of the Additional Indications Option
Commencement Exercise Notice (the foregoing period, the “Additional Indications Exercise Period”). DSP may exercise each Additional
Indications Option at any time during the Additional Indications Exercise Period by (i) providing written notice to Intercept that DSP has
obtained  required  internal  approvals  to  commence  a  pivotal  clinical  study  for  the  target  Additional  Indication  (the  “Additional
Indications Option Exercise Notice”) and (ii) making payment of the applicable fee indicated in Section 7.3.1 below to a bank account
designated  by  Intercept  (each  payment,  an  “Additional  Indications  Option  Fee”)  within  thirty  (30)  calendar  days  of  dispatch  of  the
Additional  Indications  Option  Exercise  Notice.  The  Additional  Indications  Option  shall  be  deemed  duly  exercised  on  the  date  when
Intercept has received both items (i) and (ii) (the “Additional Indications Option Effective Date”).

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7.3.1           Additional Indications Option Fee. The Additional Indications Option Fee shall be US$[***]
([***] U.S. Dollars) for each Additional Indication. For the sake of clarity, no Additional Indications Option Fee is required to be paid
upon the exercise of any Additional Indications Option in China. Upon the exercise of each Additional Indications Option, DSP shall be
entitled  to  exercise  the  rights  granted  to  it  under  Section  7.1  with  respect  to  the  target  Additional  Indication  in  the  Territory  as  it  is
constituted on the Additional Indications Option Effective Date and as it may thereafter be constituted through the exercise by DSP of
the Country Option.

7.3.2           License Grant. Following each Additional Indications Option Effective Date, (i) the definition of
“Field”  shall  be  automatically  amended  and  expanded  to  include  the  target  Additional  Indication  and  (ii)  Intercept  shall  provide  DSP
with any copies and access to any Know-How or Technology in its Control relating to the target Additional Indication.

7.3.3                      Non-Exercise  of  Additional  Indication  Option. If  DSP  declines  in  writing  to  exercise  any
particular Additional Indications Option within the Additional Indications Exercise Period, then Intercept may grant the right to a Third
Party to develop and commercialize the target Additional Indication in the Territory; provided that should any discussions with a Third
Party  not  result  in  a  binding  written  agreement  for  the  target  Additional  Indication,  then  DSP’s  Additional  Indications  Option  with
respect to such target Additional Indication shall revive and the provisions of Article 7 shall apply thereto.

7.4.          Separate Nature. For the sake of clarification, the exercise of the Additional Indications Option by DSP in
connection  with  one  of  the  Additional  Indications  shall  not  be  construed  as  relieving  Intercept  of  the  obligation  of  complying  with
Articles 7.1-7.3 above with respect to each Additional Indication.

8.          COUNTRY OPTION

8.1           Grant and Exercise of Country Option. Intercept hereby grants to DSP the exclusive option to add any or
all of the following countries to the Territory: Korea, Taiwan, Malaysia, Vietnam, the Philippines, Thailand, Singapore and Indonesia (the
“Country Option”). DSP shall have a separate exclusive option with respect to each of the countries listed in the preceding sentence, such
that the exercise by DSP of the Country Option with respect to one country shall not be deemed a waiver of its rights with respect to the
other  countries  listed  in  the  first  sentence  of  this  Section  8.1.  Upon  the  exercise  of  the  Country  Option  by  DSP  with  respect  to  any
particular country, such country shall be automatically deemed a part of the Territory. The exercise of the Country Option with respect to
one country shall automatically include all Fields in the Territory.

22

8.2           Country Option Fee. The Country Option shall be exercisable at DSP’s discretion at any time from the
Effective Date to the date of issuance of Marketing Approval for Commercialization of the Product in the Field in Japan by providing
written notice of its intent to the exercise the Country Option (the “Country Option Exercise Notice”). DSP shall pay an exercise fee of
US$[***]  ([***]  U.S.  Dollars)  per  each  country,  due  within  [***]  ([***])  [***]  following  exercise  of  the  relevant  Country  Option.
Unless exercised in accordance with this provision, or as otherwise set forth in this Agreement, the Country Option shall expire on the
date upon which Regulatory Approval for the sale of the Product in the Field in Japan is issued.

8.3           Third Party Offers. Notwithstanding the exclusive option granted to DSP in Section 8.1 hereof, following
the [***] ([***]) [***] of the Effective Date, in the event that Intercept desires to accept or make a bona fide offer from a Third Party for
the  exclusive  development  and/or  commercialization  rights  for  the  Product  in  countries  listed  in  the  first  sentence  of  Section  8.1  (the
“Target Country”), Intercept shall immediately notify DSP in writing and indicate the Target Country, desired indications, and provide a
summary of the material financial terms and conditions of the offer (the “Third Party Offer Notice”). Within forty-five (45) calendar days
of receipt of the Third Party Offer Notice, DSP shall notify Intercept in writing whether or not it wishes to exercise the Country Option
for the Target Country (the “Country Exercise Option Notice”). If DSP desires to exercise the Country Option for the Target Country,
DSP shall make the payment of the Country Option Fee for the Target Country to a bank account designated by Intercept no later than
thirty (30) calendar days following dispatch of the Country Exercise Option Notice. If DSP declines to exercise the Country Option for
the  Target  Country,  then  Intercept  shall  be  free  to  negotiate  with  the  Third  Party  on  terms  no  less  materially  favorable  than  those
contained  in  the  Third  Party  Offer  Notice;  provided  that  should  such  negotiations  fail,  then  DSP’s  Country  Option  shall  revive  with
respect to the Target Country.

8.4           Right of First Negotiation. Prior to accepting or making a bona fide offer from or to a Third Party with
respect to the exclusive development and commercialization rights for the Compound in the Field (including all Additional Indications)
in the U.S. and Canada, Intercept shall promptly deliver a written notice thereof to DSP. Intercept and DSP shall engage in good faith
negotiations, but to avoid any confusion, Intercept shall also be free to engage in good faith negotiations with such Third Party Offeror;
provided  that  should  the  parallel  discussions  between  Intercept  and  such  Third  Party  and  Intercept  and  DSP  not  result  in  a  binding
agreement, then this Right of First Negotiation shall revive with respect to any subsequent offers from or to third parties with respect to
the rights described in this Section 8.4. Further, in the event that DSP terminates the Agreement based on the cessation of development of
the Compound or the Product by Intercept, then immediately following such termination, DSP and Intercept shall engage in good faith
discussions concerning the exclusive development and commercialization rights for the Compound in the Field (including all Additional
Indications) in the U. S. and Canada.

23

9.          PAYMENTS

9.1                      Upfront  Fee.  DSP  shall  make  a  one-time,  non-refundable,  non-creditable  payment  to  Intercept  of
US$15,000,000 (Fifteen Million Dollars) (“Upfront Fee”) within thirty (30) calendar days of the Effective Date to a bank designated in
writing by Intercept. It is acknowledged that this upfront fee shall include the consideration for the rights granted to DSP in Section 8.4.
All references to “fiscal year” shall refer to the Japanese fiscal year which ends on March 31 of each calendar year and indicate that it
applies to all sub-sections in Article 9 and also Article 10.

9.2           Milestone Payments. The milestone payments set forth in this Section 9.2 shall be paid only once, upon the
first  achievement  of  the  applicable  milestone  event  in  the  applicable  listed  geographic  area.  For  purposes  of  determining  whether  a
milestone event set forth in Sections 9.2.2 and 9.2.3 has occurred (and without creating an obligation to pay the milestone more than
once as set forth in the preceding sentence), Net Sales for each fiscal year shall be aggregated for all Products sold in the Territory during
the relevant fiscal year.

the Product, DSP shall pay to Intercept each of the non-refundable, non-creditable milestone payments set forth below:

9.2.1           Within thirty (30) calendar days following the occurrence of each of the events set forth below for

Milestone Event

Development Milestones

Milestone Payment

Japan

PBC-Commencement of Phase III Clinical Trial

PBC-Marketing Approval

NASH-2nd indication-Marketing Approval

Additional Indications-Marketing Approval

China

PBC-Commencement of Phase III Clinical Trial

PBC-Marketing Approval

NASH-2nd indication-Commencement of Phase III Clinical Trial

NASH-Marketing Approval

Additional Indications-Commencement of Phase III Clinical Trial

Additional Indications-Marketing Approval

US$[***]

US$[***]

US$15,000,000.00

US$[***]

US$[***]

US$[***]

US$[***]

US$10,000,000.00

US$[***]

US$[***]

24

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
United States

PBC-Marketing Approval

NASH Successful NIH Clinical Trial

NASH-Marketing Approval

Other Asian countries

PBC-Initiation of clinical trial

PBC-Marketing Approval

Additional Indications-Initiation of clinical trial

Additional Indications-Marketing Approval

US$3,000,000.00*

US$[***]**

US$[***]***

US$[***]

US$[***]

US$[***]

US$[***]

*In the event that the WAC exceeds US$[***] per day before approval in Japan, then an amount of US$2,000,000.00 shall be paid as an
additional milestone payment (i.e., a total of US$5,000,000.00).

**The  milestone  payment  for  the  NASH  NIH  clinical  trial  is  conditioned  on  the  results  being  available  no  later  than  [***],  and
supporting a decision by the JSC to continue Development of the Product for the NASH indication.

***In the event that (i) the NASH Marketing Approval in the U.S. occurs prior to the end of 2017 (i.e., based on a sNDA submission of
the NIH clinical trial data) and DSP is able to use these data in support of a NDA submission in Japan, then the additional amount of
US$[***]  shall  be  paid  (i.e.,  a  total  of  US$[***]);  but  (ii)  if  the  NASH  Marketing  Approval  in  the  U.S.  occurs  after  the  Marketing
Approval in Japan, then no milestone payment of US$[***] as set forth in the chart above shall be due.

9.2.2           Sales Milestones. Within sixty (60) calendar days following the end of each calendar quarter in
which any event set forth below occurs, DSP shall notify Intercept of such event via the reports as indicated in Section 10.1 and within
sixty  (60)  calendar  days  following  the  end  of  such  calendar  quarter  shall  pay  to  Intercept  each  of  the  non-refundable,  non-creditable
milestone payments set forth below. For the avoidance of doubt, in the event that two or more of the events set forth below occur during
the same calendar quarter, then DSP shall pay to Intercept the aggregate of the applicable sales milestone payments set forth below in the
manner set forth in the first sentence of this Section 9.2.2.:

Net Sales exceed US$50 Million (one time only payment)  

Net Sales exceed US$100 Million (one time only payment)  

US$5,000,000.00

US$10,000,000.00

25

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Net Sales exceed US$200 Million (one time only payment)  

Net Sales exceed US$400 Million (one time payment only)

Net Sales exceed US$1,200 Million (one time payment only)

US$20,000,000.00

US$40,000,000.00

US$120,000,000.00

9.2.3           Royalty Tiers.  DSP  shall  pay  to  Intercept  a  royalty  of  [***]  percent  ([***]%)  based  on  total
annual Net Sales of all Products in the Field in the Territory for each fiscal year (i.e. ending on March 31 of each calendar year) in which
the  Net  Sales  of  all  Products  in  the  Territory  for  such  year  is  less  than  US$[***]  (the  “First  Tier  Royalty  Rate”).  DSP  shall  pay  to
Intercept a royalty of [***] percent ([***]%) based on total annual Net Sales of all Products in the Field in the Territory for each fiscal
year in which the Net Sales of all Products in the Territory for such year is US$[***] or more but less than US$[***] (the “Second Tier
Royalty Rate”). DSP shall pay to Intercept a royalty of [***] percent ([***]%) based on total annual Net Sales of all Products in the Field
in the Territory for each fiscal year in which the Net Sales of all Products in the Territory for such year exceeds US$[***] (the “Third
Tier  Royalty  Rate”).  Notwithstanding  the  foregoing,  the  transfer  price  for  the  [***]  of  the  Commercial  Supplies  to  DSP  by  Intercept
following receipt of Marketing Approval in Japan shall be calculated in accordance with Section 6.2.1 and shall be deemed to including
the running royalty payment, and accordingly no further royalty payments by DSP shall be required with respect thereto; however in no
event will the transfer price be less than the [***] percent ([***]%) plus the applicable First, Second or Third Tier Royalty Rate.

9.3           Reduced Royalty Rates for Net Sales

9.3.1                      Reduced  Royalty  Rates  in  Countries  Excluding  Japan.  If  at  any  time  [***]  of  the  First
Commercial Sale in a country in the Territory (excluding Japan), a generically equivalent product enters the market and captures more
than  [***]  percent  ([***]%)  of  the  market  share  as  determined  by  unit  sales  (“Market  Share”)  for  [***],  then  the  country  shall  be
designated an “Eroded Country” beginning the first day of the next calendar quarter. For the purpose of determining royalty payments
due on an Eroded Country’s Net Sales, total annual Net Sales will be assessed country-by-country and not aggregated with other country
Net Sales in the Territory. The reduced royalty rates that shall apply in an Eroded Country are as follows:

i.    Eroded Country Net Sales up to US$[***] assessed at [***] percent ([***]%); and
ii.   Eroded Country Net Sales of US$[***] up to (but less than) US$[***] assessed at [***]

percent ([***]%); and

iii.  Eroded Country Net Sales of US$[***] or more assessed at [***] percent ([***]%).

Thereafter, DSP’s Market Share in each subsequent calendar quarter will be assessed and if the Market Share is restored to [***] percent
([***]%)  or  above  then  the  royalty  rates  set  forth  in  Section  9.2.3  shall  apply  again  to  Net  Sales  in  that  country,  which  shall  be
aggregated with all other Net Sales (excluding Eroded Country Net Sales), and if the Market Share remains or falls back below [***]
([***]%) in any calendar quarter, then the Eroded Country reduced royalty rates set forth in this Section 9.3.1 shall apply. The JSC shall
be responsible for determining the most effective means to implement an effective Market Share, Net Sales and royalty tracking system
in the Territory in order to give effect to DSP’s royalty payment obligations hereunder.

26

 
 
 
 
 
 
 
 
 
9.3.2           Reduced Royalty Rates in Japan. The royalty rates set forth in Section 9.2.3 shall remain in
effect with respect to total annual Net Sales in Japan until such time as (i) the substance patent in Japan expires (after taking into account
all available extensions) and (ii) a generically equivalent product enters the market and captures more than [***] percent ([***]%) of the
Market Share for [***]. Thereafter, beginning the first day of the next calendar quarter, Japan shall be designated an Eroded Country and
DSP shall pay Intercept a reduced royalty of [***] percent ([***]%) on total annual Net Sales in Japan for [***] of such designation,
[***] percent ([***]%) on total annual Net Sales for the [***] of such designation, and then [***] percent ([***]%) on total annual Net
Sales thereafter. Once Japan has been designated as an Eroded Country, DSP’s Market Share in each subsequent calendar quarter will be
assessed  and  if  the  Market  Share  is  restored  to  [***]  percent  ([***]%)  or  above  then  the  royalty  rates  set  forth  in  Section  9.2.3  shall
apply again to Net Sales in Japan, which shall be aggregated with all other Net Sales (excluding Eroded Country Net Sales), and if the
Market Share remains or falls back below [***] percent ([***]%) then the Eroded Country reduced royalty rates set forth in this Section
9.3.2 shall apply at the applicable royalty rate based on the cumulative number of quarters that had previously passed while Japan had
been designated an Eroded Country. The JSC shall be responsible for determining the most effective means to implement an effective
Market  Share,  Net  Sales  and  Royalty  tracking  system  in  the  Territory  in  order  to  give  effect  to  DSP’s  royalty  payment  obligations
hereunder.

9.4           Necessary Third Party Technology Payments. DSP shall be entitled to deduct [***] percent ([***]%) of
all  royalties  it  is  required  to  pay  to  a  Third  Party  for  Necessary  Third  Party  IP  under  any  agreement  to  license  or  acquire  intellectual
property used in the Development or Commercialization of the Product in the Field in the Territory up to a maximum of [***] percent
([***]%) for purposes of Section 9.2.3, or [***] percent ([***]%) for purposes of Section 9.3.1 or 9.3.2 of the applicable royalty rate.

10.         PAYMENT; RECORDS; AUDITS

10  .1                  Payment; Reports. Royalties  shall  be  calculated  and  reported  during  the  fiscal  year  for  each  calendar
quarter. All payments due to Intercept under this Agreement shall be paid within sixty (60) calendar days after the end of each calendar
quarter. DSP shall deliver to Intercept (i) within thirty (30) calendar days after the end of each calendar quarter a report of gross sales of
Product in the Territory and (ii) within sixty (60) days after the end of each calendar quarter, a report certified by DSP as accurate to the
best  of  its  ability  based  on  information  then  available  to  DSP,  setting  forth  for  such  calendar  quarter  the  following  information  on  a
country-by-country basis and other such information to permit confirmation of the accuracy of the information for which payments are
calculated including: (i) gross and Net Sales of Product, (ii) the basis for any adjustments to the royalty payable for the sale of Product,
and (iii) the royalty due hereunder for the sale of Product. All payments hereunder shall be payable in U.S. dollars. All payments owed
under  this  Agreement  shall  be  made  by  wire  transfer  in  immediately  available  funds  to  a  bank  and  account  designated  in  writing  by
Intercept.  Conversion  of  foreign  currency  to  U.S.  Dollars  shall  be  made  at  the  Telegraphic  Transfer  Selling  (TTS)  rate  published  by
Sumitomo Mitsui Banking Corporation or any other mutually agreed upon source, in effect on the last day of each calendar month within
each calendar quarter to the Net Sales that was deemed sold during such month with respect to royalty and sales milestones payments
under Sections 9.2.2 and 9.3 and for the previous day of the notification of the development milestone under Section 9.2.1.

27

  
10.2         Tax Withholding. Intercept shall be responsible for any income taxes payable by Intercept on payments
made  to  it  under  this  Agreement.  If  applicable  Laws  require  that  taxes  be  deducted  and  withheld  from  a  payment  due  from  DSP  to
Intercept under this Agreement, DSP shall (i) deduct those taxes from the payment; (ii) pay the taxes to the proper taxing authority; and
(iii)  send  evidence  of  the  proof  of  payment  to  Intercept  promptly  following  that  payment.  Intercept  shall  provide  DSP  with
documentation  necessary  for  DSP  to  file  an  application  with  the  applicable  tax  authorities  to  avoid  or  reduce  withholding  or  other
applicable taxes under any applicable tax treaty.

10.3         Audits. During the Term and for a period of three (3) years thereafter, DSP shall keep (and shall cause its
Affiliates and sublicensees to keep) complete and accurate records pertaining to the sale or other disposition of Products in the Field in
the Territory and calculations of Net Sales and payments required under this Agreement in sufficient detail to permit Intercept to confirm
the accuracy of all payments due to it hereunder. Notwithstanding the foregoing, should applicable Law in the Territory require DSP to
retain records of the nature described in the preceding sentence for a period longer than that set forth in the preceding sentence, DSP
shall  retain  such  records  for  the  longer  period;  provided  that  Intercept  shall  advise  of  any  applicable  record-keeping  requirements
imposed  by  laws  outside  the  Territory.  Intercept  shall  have  the  right  to  cause  an  independent,  certified  public  accountant  reasonably
acceptable to DSP to audit such records to confirm Net Sales, royalty, milestone and other payments for a period covering up to but not
more  than  the  preceding  twelve  (12)  calendar  quarters;  provided  that  any  such  accountant  shall  have  previously  entered  into  a
confidentiality agreement reasonably satisfactory to DSP limiting its disclosure of such information to authorized representatives of the
Parties or as required under applicable Laws. Any such inspection shall be for the sole purpose of verifying the calculation of payments
on  Net  Sales  of  the  Products  in  the  Field  in  the  Territory  by  DSP,  and  its  Affiliates  or  sublicensees  and  milestone,  royalty  and  other
payments paid by DSP under this Agreement. The accountant shall only disclose to Intercept the findings of the audit and the specific
details  concerning  any  discrepancies.  No  other  information  shall  be  provided  to  Intercept.  Such  audit  rights  may  be  exercised  during
normal business hours upon reasonable prior written notice to DSP; provided that such audit right may be exercised no more than once in
any twelve (12) -month period. Prompt adjustments shall be made by the Parties to reflect the results of such audit. Intercept shall bear
the full cost of such audit unless such audit discloses an underpayment by DSP of more than [***] percent ([***]%) of the amount of
royalties or other payments due under this Agreement, in which case, DSP shall bear the full cost of such audit.

28

11.         TREATMENT OF CONFIDENTIAL INFORMATION

11.1         Confidential Obligations. DSP and Intercept each recognize that the other Party’s Confidential Information
constitutes  highly  valuable  and  proprietary  confidential  information.  Intercept  and  DSP  each  agree  that  during  the  Term  of  this
Agreement and for five (5) years thereafter, it will keep confidential, and will cause its employees, consultants, contractors, Affiliates and
sublicensees to keep confidential, all Confidential Information of the other Party. Neither Intercept nor DSP, nor any of their respective
employees, consultants, Affiliates or sublicensees shall use Confidential Information of the other Party for any purpose whatsoever other
than exercising any rights granted to it or reserved by it hereunder. Without limiting the foregoing, each Party may disclose information
to the extent such disclosure is reasonably necessary to (i) file and prosecute patent applications and/or maintain patents which are filed
or  prosecuted  in  accordance  with  the  provisions  of  this  Agreement,  or  (ii)  file,  prosecute  or  defend  litigation  in  accordance  with  the
provisions  of  this  Agreement  or  (iii)  comply  with  applicable  Laws,  regulations  or  court  orders;  provided,  however,  that  if  a  Party  is
required to make any such disclosure of the other Party’s Confidential Information in connection with any of the foregoing, it will give
reasonable advance notice to the other Party of such disclosure requirement and will use reasonable efforts to assist such other Party in
efforts to secure confidential treatment of such information required to be disclosed.

11.2         Publication. If either Party plans to publish or present the results of any studies or other data regarding the
Compound,  the  Product  or  Additional  Indications  conducted  in  and  outside  the  Territory,  the  Party  shall  submit  the  draft  of  the
publication, translated into English, to the other no later than four (4) weeks prior to the planned submission for publication for approval,
unless such disclosure requires immediate publication due to disclosure requirements of the U.S. Securities and Exchange Commission,
the NASDAQ stock exchange or any other stock exchange on which securities issued by a Party are traded and Intercept has advised
DSP of the deadline for disclosure in a sufficiently timely manner. As soon as a Party is aware of a deadline for submitting an abstract for
an

upcoming  scientific  meeting,  it  shall  notify  the  other  Party  in  writing  and  the  Parties  shall  use  Commercially  Reasonable  Efforts  to
exchange  comments  on  the  proposed  abstract  in  a  timely  manner  to  facilitate  the  publication/presentation  of  the  proposed  abstract.
Otherwise, any publication shall need the other Party’s prior written consent, which shall not be unreasonably withheld. Any comment,
reasonable request for modification or reasonable rejection must be made within as quickly as practically possible from the receipt of the
draft. Failure to quickly make such comments shall be conclusively deemed to constitute approval of such publication or presentation.
For  the  avoidance  of  doubt,  this  Section  11.2  shall  apply  to  publications  made  by  either  Party  both  in  the  Territory  and  outside  the
Territory.

11.3                  Publicity.  DSP  and  Intercept  may,  by  mutual  written  agreement,  issue  a  press  release  announcing  the
execution of this Agreement, which shall be substantially in a form approved by the Parties. Except with respect to such initial release or
as  otherwise  required  by  applicable  Laws  (including  disclosure  requirements  of  the  U.S.  Securities  and  Exchange  Commission,  the
NASDAQ  stock  exchange  or  any  other  stock  exchange  on  which  securities  issued  by  a  Party  are  traded),  neither  Party  shall  issue  an
additional press release or public announcement relating to this Agreement without the prior written approval of the other Party, which
shall not be unreasonably withheld or delayed. In the event that a Party wishes to refer to the other Party or the transactions under this
Agreement in promotional or other communications with prospective customers and investors, such Party shall first provide the other
Party with advance notice of such proposed disclosure and the form, substance and intended use of such proposed disclosure and obtain
the prior written approval of the other Party to the form, substance and intended use of such proposed disclosure.

29

12.         FILING, PROSECUTION AND MAINTENANCE OF PATENT RIGHTS

12.1         Patent Filing, Prosecution and Maintenance. Subject to the other terms of this Section 12.1, Intercept shall
be  responsible  for  preparing,  filing,  prosecuting,  obtaining  and  maintaining,  all  Intercept  Patents  in  the  Territory.  Intercept  (i)  will
provide DSP with a copy of any proposed patent application or prosecution or other document relating to a patent or application within
the Intercept Patents and to the Field (and the Additional Indications) for review and comment reasonably in advance of filing which
shall  under  no  circumstances  be  less  than  thirty  (30)  days,  and  (ii)  will  keep  DSP  reasonably  informed  of  the  status  of  such  filing,
prosecution and maintenance.

12.2         Enforcement. If, during the Term, either Party learns of any actual, alleged or threatened infringement by a
Third Party of any Intercept Patent under this Agreement, such Party shall promptly notify the other Party and shall provide such other
Party with available evidence of such infringement. Intercept shall have the first right (but not the obligation), at its own expense and
with  legal  counsel  of  its  own  choice,  to  bring  suit  (or  take  other  appropriate  legal  action)  against  any  actual,  alleged  or  threatened
infringement of the Intercept Patent in the Field in the Territory; provided that the settlement of such matter shall require DSP’s consent,
not to be unreasonably withheld or delayed. DSP shall have the right, at its own expense, to be represented in any such action by counsel
of  DSP’s  own  choice.  If  Intercept  does  not  file  any  action  or  proceeding  against  any  such  material  infringement,  with  material
infringement  determined  using  reasonable  commercial  standards  (including  obtaining  the  advice  of  patent  counsel),  within  three  (3)
months after the later of (i) DSP’s notice to Intercept hereunder, (ii) Intercept’s notice to DSP hereunder, or (iii) a written justified request
from DSP to take action with respect to such infringement, then DSP shall have the right (but not the obligation), at its own expense, to
bring suit (or take other appropriate legal action) against such actual, alleged or threatened infringement, with legal counsel of its own
choice,  including  the  right  to  settle  any  such  suit  without  the  prior  consent  of  Intercept,  who  shall  render  all  assistance  reasonably
required or requested by DSP. Irrespective of which party is taking the lead with respect to the defense of a claim, the party taking the
lead shall keep the other party reasonably informed as to the status of any such action and shall give due regard to the comments and
suggestions of the other Party with respect to the defense of such claims. Any damages, monetary awards or other amounts recovered,
whether by judgment or settlement, pursuant to any suit, proceeding or other legal action taken under this Section 12.2, shall applied as
follows:

fees and costs and costs for providing assistance) incurred in prosecuting such enforcement action, and

(a)          first, to reimburse the Parties for their respective costs and expenses (including reasonable attorneys’

30

(b)          second, any amounts remaining shall be allocated [***] percent ([***]%) to the Party initiating the
legal action and [***] percent ([***]%) to the other Party, if the other Party provides material assistance, as determined using reasonable
commercial standards, and if not then, [***] ([***]%) to the initiating Party.

If a Party brings any such action or proceeding hereunder, the other Party agrees to be joined as party plaintiff if necessary to prosecute
such  action  or  proceeding,  and  to  give  the  Party  bringing  such  action  or  proceeding  reasonable  assistance  and  authority  to  file  and
prosecute the suit; provided, however, that neither Party shall be required to transfer any right, title or interest in or to any property to the
other Party or any Third Party to confer standing on a Party hereunder.

12.3         Defense. Each Party shall promptly notify the other Party in writing of any allegation by a third Party that the
activity of either of the Parties or their Affiliates or sublicensees pursuant to this Agreement infringes or may infringe the intellectual
property rights of such Third Party. Intercept shall have the right to control, at its own expense, the defense of any claim alleging that the
Development, Manufacturing or Commercialization of the Product in the Field in the Territory infringes any such Third Party rights. If
Intercept fails to proceed in a timely manner with respect to such defense, DSP shall have the option to assume control the defense of
such claim. As a general matter, the Parties acknowledge that Intercept, as the licensor of the Intercept Technology shall, in principle, be
responsible for all costs associated with maintaining validity of the Intercept Technology. Nonetheless, in light of the fact that Intercept is
in  an  early-stage  development  company,  DSP  is  willing  to  bear  [***]  percent  ([***]%)  of  reasonable  and  actual  costs  and  expenses
incurred by DSP in connection with any defense of which DSP assumes control (the “DSP Defense Costs”), with the remainder being
reimbursed by Intercept in the form of reduced royalties owed to it from DSP pursuant to Section 9.3, provided that in the event of an
Intercept  Change  of  Control,  DSP  may  reduce  the  percentage  of  DSP  Defense  Costs  for  which  DSP  is  responsible.  Notwithstanding
anything to the contrary herein, from the [***] ([***]) anniversary of the Effective Date, the preceding proviso shall become null and
void, such that Intercept shall be fully responsible for all actual and reasonable costs incurred by DSP in any defense which it assumes
pursuant to this Section 12.3. Irrespective of which Party is taking the lead with respect to the defense of a claim, the Party taking the
lead shall keep the other Party reasonably informed as to the status of any such action and shall give due regard to the comments and
suggestions of the other Party with respect to the defense of such claims. DSP shall have the right to participate in the defense of any
such claim with counsel of its choice at its own expense. Intercept shall not have the right to settle any claim or litigation described in
this Section 12.3 without the consent of DSP, such consent not to be unreasonably withheld; notwithstanding which, in the event that
DSP assumes control of the defense of any such claim in accordance with this Section 12.3, then DSP shall be entitled to settle such
matter in its reasonable discretion. If a Party brings any such action or proceeding hereunder, the other Party agrees to be joined as party
plaintiff  if  necessary  to  prosecute  such  action  or  proceeding,  and  to  give  the  Party  bringing  such  action  or  proceeding  reasonable
assistance and authority to file and prosecute the suit; provided, however, that neither Party shall be required to transfer any right, title or
interest in or to any property to the other Party or any Third Party to confer standing on a Party hereunder.

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12.4         Ownership of Improvements. Intercept  shall  solely  own  all  Improvements  that  are  made,  conceived  or
reduced  to  practice  solely  by  one  or  more  employees  or  contractors  of  either  Intercept  arising  in  connection  with  the  performance  by
Intercept of its obligations hereunder. Intercept hereby grants to DSP the exclusive right to use all such Intercept Improvements in the
Territory during the Term of this Agreement. DSP shall solely own all Improvements that are made, conceived or reduced to practice
solely by one or more employees or contractors of DSP arising in connection with the performance by DSP of its obligations hereunder.
DSP hereby grants to Intercept the non-exclusive right to use all such DSP Improvements outside the Territory during the Term of this
Agreement. Each of DSP and Intercept shall have the right, in its discretion, but subject to the terms and conditions of this Agreement, to
file patents applications with respect to their respective Improvements.

12.5         Joint Improvements.

12.5.1           Ownership and Disclosure. DSP and Intercept shall be joint owners in and to any and all Joint
Improvements  and  any  Patents  claiming  such  Joint  Improvements.  Subject  to  the  terms  and  conditions  of  this  Agreement,  DSP  and
Intercept,  as  joint  owners  of  the  Joint  Improvements,  shall  have  the  right  to  practice  and  exploit  the  Joint  Improvements  without  any
obligation to account to the other for profits. Any assignment of an interest in a Joint Improvement shall require the prior consent of the
other Party, such consent not to be unreasonably withheld. Each Party agrees to be named as a party, if necessary, to bring or maintain a
lawsuit involving a Joint Improvement. Each Party shall promptly report to the other Party in writing, through the JSC, and shall cause its
Affiliates,  licensees  (including  sublicensees),  and  contractors  (including  subcontractors)  to  so  disclose,  the  invention  or  conception  of
any Joint Improvements.

12.5.2           Prosecution and Maintenance.

(i)   Inside the Territory, DSP shall have the first right to prepare, file, prosecute and maintain Joint
Improvements at its own cost and expense. Through its progress reports submitted to the JSC pursuant to Section 3.5, DSP shall keep
Intercept  informed  of  the  status  of  all  filings  related  to  the  Joint  Improvements  (including  the  nature  of  any  objections  and  other
information reasonably requested by Intercept) and will provide Intercept with copies, in either English or Japanese, of all substantive
documentation submitted to, or received from, the patent offices in connection therewith. DSP shall provide Intercept with the right to
comment on the documentation. The Parties shall cooperate reasonably in the prosecution of all Patents covering the Joint Improvements
if practicably possible and shall share all material information relating thereto promptly after receipt of such information. If during the
Term of this Agreement, DSP intends to allow any Patent claiming a Joint Improvement to expire or intends to otherwise abandon any
such Patent in the Territory, or decides not to file patent applications covering or claiming a Joint Invention in the Territory, DSP shall
notify Intercept of such intention or decision at least ninety (90) days prior to any filing or payment due date, or any other that requires
action,  in  connection  with  such  Patent  in  the  Territory,  and  Intercept  shall  thereupon  have  the  right,  but  not  the  obligation  to  assume
responsibility for the preparation, filing, prosecution or maintenance thereof at its sole cost and expense, in the name of and solely owned
by Intercept.

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(ii)   Outside the Territory, Intercept shall have the first right to prepare, file, prosecute and maintain
Joint  Improvement  at  its  own  cost  and  expense.  Intercept  shall  keep  DSP  informed  of  the  status  of  all  filings  related  to  the  Joint
Improvement  and  will  provide  Intercept  with  copies,  in  either  Japanese  or  English,  of  all  substantive  documentation  submitted  to,  or
received from, the patent offices in connection therewith. Intercept shall provide DSP with the right to comment on the documentation.
The Parties shall cooperate reasonably in the prosecution of all Patents covering the Joint Improvement if practicably possible and shall
share all material information relating thereto promptly after receipt of such information. If during the term of this Agreement, Intercept
intends to allow any Patent claiming a Joint Improvement to expire or intends to otherwise abandon any such Patent outside the Territory,
or  decides  not  to  file  patent  applications  covering  or  claiming  a  Joint  Invention  in  the  Territory,  Intercept  shall  notify  DSP  of  such
intention or decision at least ninety (90) days prior to any filing or payment due date, or any other that requires action, in connection with
such  Patent  outside  the  Territory,  and  DSP  shall  thereupon  have  the  right,  but  not  the  obligation  to  assume  responsibility  for  the
preparation, filing, prosecution or maintenance thereof at its sole cost and expense, in the name of and solely owned by DSP.

12.5.3           Enforcement; Defense. Through the JSC, the Parties shall develop a process to coordinate the
defense of Patents claiming a Joint Improvement, including cost-sharing allocation, both inside and outside the Territory; provided that
should the Parties be unable to resolve any disagreement regarding the defense of a Patent claiming a Joint Improvement, such issue shall
be resolved in accordance with Section 12.5.4.

12.5.4           Ownership and Other Disputes. The JSC shall resolve any issues regarding inventorship or
ownership of Joint Improvements and the defense of any Patent claiming a Joint Improvement pursuant to the provisions of Article 12. In
connection with the resolution of this issue, each Party is entitled to have a patent lawyer of its own choosing attend the meeting and
submit its written legal opinion. In the event that the JSC is unable to reach a decision, the matter shall be referred for resolution to a
patent counsel, reasonably acceptable to both Parties, who is affiliated with a firm of international repute. The decision of such patent
attorney shall be rendered in writing and shall be final and binding on the parties. Each Party shall bear its own costs and expenses for
legal advice provided to it in accordance with the second sentence of this Section 12.5.3. All costs and expenses incurred in connection
with the mutually appointed patent attorney shall be shared equally.

12.6         Trademarks. DSP shall own and have sole control over all matters relating to the use of all trademarks (and
all associated goodwill) used in the sale of Products in the Field in the Territory. DSP shall be solely responsible for trademark searches,
prosecution of applications to register and to record licenses (if applicable), and maintenance of the Product-related trademarks in the
Territory as well as costs and expenses incurred in connection with the foregoing. If Intercept becomes aware of any actual or threatened
infringement of any Product-related trademark by a Third Party, it shall promptly notify DSP, who shall be responsible for enforcing the
Product-related trademarks.

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13.         REPRESENTATIONS, WARRANTIES AND COVENANTS

throughout the Term of this Agreement:

13.1         Intercept’s Representations. Intercept represents and warrants to DSP that as of the Effective Date and

hereby have been duly authorized by all appropriate Intercept corporate action;

(a)          The execution and delivery of this Agreement and the performance of the transactions contemplated

(b)          This Agreement is a legal and valid obligation binding upon Intercept and enforceable in accordance
with its terms, and the execution, delivery and performance of this Agreement by the Parties, and does not conflict with any agreement,
instrument or understanding to which Intercept is a party or by which it is bound;

(c)          Intercept has, to the best of its knowledge, the full right and legal capacity to grant the rights granted
to DSP hereunder without violating the rights of any Third Party, and is the sole and exclusive owner of the Intercept Technology and the
Intercept Manufacturing Technology, all of which are free and clear of any liens, charges and encumbrances.

(d)                   To  Intercept’s  best  knowledge,  there  are  no  pending  legal  actions,  nor  is  Intercept  aware  of  the
receipt of any written notice regarding any pending legal actions or threatened claims (including pending re-examination, opposition or
interference), with respect to the Intercept Technology or the Intercept Manufacturing Technology, or litigation seeking to invalidate any
Intercept Technology or any Intercept Manufacturing Technology;

(e)          Intercept owns the Intercept Patents listed on Exhibit A, has not assigned, transferred, conveyed or
otherwise encumbered its right, title and interest in the Intercept Patents, Intercept Know-How, or Intercept Manufacturing Technology in
the Territory.

Party under the Intercept Technology or the Intercept Manufacturing Technology that conflict with the rights granted to DSP hereunder.

(f)          Intercept has not granted, and during the Term of this Agreement will not grant, rights to any Third

(g)          Intercept is not aware of any safety, efficacy, or regulatory issues, other than the information that has
previously  been  made  available  to  DSP  in  writing  that  would  preclude  DSP  from  Developing,  Manufacturing,  or  otherwise
Commercializing the Products in the Field in the Territory.

and the Intercept Manufacturing Technology shall not infringe any patent or other intellectual property right of any Third Party.

(h)          To Intercept’s best knowledge, DSP’s exercise of its rights with respect to the Intercept Technology

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(i)                   All  material  Development  activities  with  respect  to  the  Product  whether  clinical,  non-clinical  or
preclinical conducted by Intercept or at its request, has been, and shall be conducted in compliance with all applicable Law, including but
not limited to Good Manufacturing Practices, Good Clinical Practice and Good Laboratory Practices.

13.2         DSP Representations. DSP represents and warrants to Intercept that as of the Effective Date:

hereby have been duly authorized by all appropriate DSP corporate action; and

(a)          the execution and delivery of this Agreement and the performance of the transactions contemplated

(b)          this Agreement is a legal and valid obligation binding upon DSP and enforceable in accordance with
its terms, and the execution, delivery and performance of this Agreement by the Parties does not conflict with any agreement, instrument
or understanding to which DSP is a party of or by which it is bound.

Intercept Manufacturing Technology shall not infringe any patent or other intellectual property right of any Third Party.

(c)          to DSP’s knowledge, DSP’s exercise of its rights with respect to the Intercept Technology and the

13.3                  Change  of  Control  Covenant. Intercept  shall  provide  DSP  with  prior  written  notice  of  a  proposed  or
contemplated Intercept Change of Control and shall use Commercially Reasonable Efforts to afford DSP an opportunity to meet with the
potential acquirers (or the like) to discuss any necessary or advisable amendments to this Agreement no later than 60 days prior to the
effective date of the Intercept Change of Control.

13.4         Competitive Products. DSP shall not engage, directly or indirectly, in the commercialization of any other
product  FXR  agonist  compound  or  product  in  the  Field  within  the  Territory.  For  the  avoidance  of  doubt,  this  does  not  include
manufacturing, research or development activities. Further, this provision shall not apply to any country in the Territory or any indication
with respect to which the nature of the rights granted to DSP under this Agreement are converted to non-exclusive rights by Intercept
pursuant to Section 15.2(c) of this Agreement.

13.5         No Warranties.

Nothing in this Agreement is or shall be construed as:

application or patent licensed hereunder or

(a)          a warranty or representation by either Party as to the validity, enforceability, or scope of any patent

license granted pursuant to this Agreement is or will be free from infringement of patents, copyrights, and other rights of third parties.

(b)                    a  warranty  or  representation  that  anything  made,  used,  sold  or  otherwise  disposed  of  under  any

35

EXCEPT  AS  EXPRESSLY  SET  FORTH  IN  THIS  AGREEMENT,  NEITHER  PARTY  MAKES  ANY
REPRESENTATION OR EXTENDS ANY WARRANTIES OF ANY KIND, EITHER EXPRESS OR IMPLIED. THERE ARE
NO EXPRESS OR IMPLIED WARRANTIES OF MERCHANTABILITY OR FITNESS FOR A PARTICULAR PURPOSE, OR
OF NON-INFRINGEMENT OF ANY PATENT, COPYRIGHT, TRADEMARK, OR OTHER RIGHTS OF THIRD PARTIES,
OR ANY OTHER EXPRESS OR IMPLIED WARRANTIES.

14.         INDEMNIFICATION

14.1         Indemnification.

14.1.1           DSP Indemnity. DSP shall indemnify, defend and hold harmless Intercept and its Affiliates and
their respective directors, officers, employees, stockholders and agents and their respective successors, heirs and assigns (the “Intercept
Indemnitees”) from and against any liability, damage, loss or expense (including reasonable attorneys’ fees and expenses of litigation)
incurred  by  or  imposed  upon  such  Intercept  Indemnitees,  or  any  of  them,  in  connection  with  any  Third  Party  claims,  suits,  actions,
demands  or  judgments,  including,  without  limitation,  personal  injury  and  product  liability  matters,  to  the  extent  arising  out  of  (i)  the
Development, Manufacture, or Commercialization or use by any person of any the Product Manufactured or sold by DSP or any Affiliate
or sublicensee under this Agreement, (ii) any material breach of this Agreement by DSP, or (iii) the negligence or willful misconduct on
the  part  of  DSP  or  any  Affiliate  or  sublicensee,  in  any  such  case  under  this  Section  14.1.1,  except  to  the  extent  of  Intercept’s
responsibility therefor under Section 14.1.2 below.

14.1.2           Intercept Indemnity. Subject to Section 14.1.1 above, Intercept shall indemnify, defend and
hold harmless DSP, its Affiliates and their respective directors, officers, employees, and agents, and their respective successors, heirs and
assigns  (the  “DSP  Indemnitees”),  from  and  against  any  liability,  damage,  loss  or  expense  (including  reasonable  attorneys’  fees  and
expenses of litigation) incurred by or imposed upon such DSP Indemnitees, or any of them, in connection with any Third Party claims,
suits, actions, demands or judgments, including, without limitation, personal injury and product liability matters, to the extent arising out
of (i) the Manufacture of any the Product Manufactured or by or on behalf of Intercept, (ii) any actions or omissions of Intercept or its
Affiliates under this Agreement, (iii) any material breach of this Agreement by Intercept, or (iv) the negligence or willful misconduct on
the part of Intercept or any Affiliate, except to the extent of DSP’s responsibility therefore under Section 14.1.1 above.

36

14.2         Indemnification Procedures. In the event that any Indemnitee is seeking indemnification under Section 14.1
above from a Party (the “Indemnifying Party”), the other Party shall notify the Indemnifying Party of such claim with respect to such
Indemnitee as soon as reasonably practicable after the Indemnitee receives notice of the claim, and the Party (on behalf of itself and such
Indemnitee) shall permit the Indemnifying Party to assume direction and control of the defense of the claim (including the right to settle
the claim solely for monetary consideration) and shall cooperate as requested (at the expense of the Indemnifying Party) in the defense of
the claim. The indemnification obligations under Article 14 shall not apply to any harm suffered as a direct result of any delay in notice
to the Indemnifying Party hereunder or to amounts paid in settlement of any claim, demand, action or other proceeding if such settlement
is effected without the consent of the Indemnifying Party, which consent shall not be withheld or delayed unreasonably. The Indemnitee,
its employees and agents, shall reasonably cooperate with the Indemnifying Party and its legal representatives in the investigation of any
claim, demand, action or other proceeding covered by Section 14.1.

14.3                  Limitation on Liability.  NEITHER  PARTY  SHALL  BE  LIABLE  TO  THE  OTHER  PARTY  FOR
LOSS, DAMAGE, OR LIABILITY WITH RESPECT TO LOSS OF PROFIT, SPECIAL, INDIRECT, CONSEQUENTIAL, OR
PUNITIVE DAMAGE.

15.         TERM AND TERMINATION

15.1         Term; Expiration. The term of this Agreement (the “Term”) shall commence on the Effective Date and
expire on a country-by-county basis on the later to occur of (i) the tenth (10th) anniversary of the First Commercial Sale of the Product
for the first or second indication in such country (whichever is later) or (ii) the expiration date of the Exclusive Period in such country.
The Agreement as a whole shall expire on the date upon which the Agreement terminates with respect to the last country in the Territory.

15.2         Material Breach. (a) In the case that one of the Parties believes that the other Party has materially breached
the Agreement, the JSC shall be notified and meet as soon as possible in order that the Parties attempt to resolve any dispute as to the
thirty  (30)  days  of  receiving  the  matter  for
existence  of  any  such  material  breach.  Failing  a  consensus  decision  by  the  JSC  within  
review, it shall then be referred for “Executive Negotiation” as set forth in Article 16.1. Failing a decision by the business executives
within sixty (60) days of receiving the matter for review from the JSC, the non-breaching Party may then proceed to give written notice
of termination for material breach.

(b)          If pursuant to Section 15.2(a), either Party gives written notice to the other Party of termination for
material breach, which notice shall describe such material breach in reasonable detail and whether it has been deemed non-curable or
curable  by  the  JSC  and  senior  executives,  this  Agreement  and  the  rights  and  options  granted  herein  may  be  terminated  by  the  non-
breaching Party, effective ten (10) days after giving written notice to the breaching Party of termination for non-curable breach, thirty
(30) days after giving written notice to the breaching Party of such termination in the case of a curable payment breach, and sixty (60)
days  after  giving  written  notice  to  the  breaching  Party  of  such  termination  in  the  case  of  any  other  curable  breach.  The  foregoing
notwithstanding,  if  any  curable  material  breach  is  cured  within  the  aforesaid  thirty  (30)  or  sixty  (60)  day  period,  the  notice  shall  be
automatically withdrawn and of no effect.

37

(c)          Any exercise by Intercept or DSP of its rights under Section 15.2(b) may be on a country-by-country
or indication-by-indication basis, at Intercept’s discretion, or DSP discretion, in which case such termination shall be partial in nature and
shall only apply to the particular country or indication which is the source of the alleged material breach. Furthermore, Intercept shall
have  the  alternative  option,  in  its  sole  discretion,  instead  of  terminating  the  Agreement  in  part  or  in  whole,  to  convert  the  exclusive
appointment of DSP under Section 2 of this Agreement into a non-exclusive appointment, and to apply such non-exclusive status on a
country-by-country or indication-by-indication basis, at Intercept’s sole discretion, in which case such non-exclusivity shall only apply to
the particular country or indication which is the source of the alleged material breach.

15.3         Voluntary Termination. DSP shall have the right to terminate this Agreement at any time upon ninety (90)
days’ written notice to Intercept, either in its entirety or on a country-by-country basis or indication-by-indication basis, at the discretion
of DSP.

15.4         Effects of Termination.

15.4.1    Upon  the  expiration  of  this  Agreement  or  any  termination  of  the  entire  Agreement  by  DSP  under
Section  15.2,  as  of  the  effective  date  of  such  expiration  or  termination,  DSP  thereafter  automatically  shall  have  a  perpetual,  fully
sublicensable  and  transferable,  exclusive  license  in  the  Territory  under  the  Intercept  Technology  and  Intercept  Manufacturing
Technology,  to  Develop,  have  Developed,  make,  have  made  (including  Manufacture),  use,  have  used,  sell,  have  sold,  offer  for  sale,
import  and  have  imported  or  otherwise  Commercialize  any  and  all  Products  and  to  practice  the  Intercept  Technology  and  the
Manufacturing Technology in the Territory. Such license shall not be fully paid-up, but instead shall be payable as follows (subject to
Intercept making the transfer of the relevant Manufacturing Technology to DSP):

(a)          if before the First Commercial Sale, then [***] percent ([***]%) of royalties that would
have become due under Section 9 of this Agreement but for the termination or expiration, for a period equal to the remainder of the Term
of the Agreement, had the Agreement not been terminated;

(b)          if after the First Commercial Sale, then [***] percent ([***]%) of royalties that would have
become due under Section 9 of this Agreement but for the termination or expiration, for a period equal to the remainder of the Term of
the  Agreement,  had  the  Agreement  not  been  terminated;  provided,  however,  that  in  the  event  Intercept  does  not  comply  with  its
obligations under the Commercial Supply Agreement, the applicable rate will be [***] percent ([***]%).

(c)                   At  the  end  of  the  period  equal  to  the  remainder  of  the  Term  of  the  Agreement,  had  the
Agreement not been terminated, the exclusive license shall be deemed fully paid-up. Intercept shall disclose to DSP all material research,
non-clinical and clinical data on Products generated prior to the termination date outside the Territory and DSP shall thereafter have the
unrestricted  right  to  use  such  data  and  information  in  the  Territory.  Intercept  shall  promptly  provide  to  DSP  any  other  material,
information, contracts, etc. which Intercept owns or Controls related to the Intercept Product in the Territory and are reasonably required
to allow DSP to continue the Development, Manufacture and Commercialization of Products in the Territory with minimal delay.

38

(d)          The foregoing notwithstanding, in the case that DSP determines, in its sole discretion, upon
termination of the Agreement pursuant to this Section 15.4.1 to cease all Development, Manufacturing and Commercialization activities
relating to the Compound and the Product, then all licenses and sublicenses shall revert in full to Intercept and DSP shall have no further
payment obligations to Intercept. To give effect to the reversion of the licenses and sublicenses, DSP shall be bound by its obligations
pursuant  to  Section  15.4.2  below,  except  that  DSP  shall  not  be  bound  to  disclose  to  Intercept  all  material  research,  non-clinical  and
clinical data (except for safety data) on Products generated prior to the termination date, nor shall DSP be bound to assign all Regulatory
Filings relating to Products in the Territory.

15.4.2       Upon any termination of the Agreement by Intercept under Section 15.2 , or upon any termination
of the Agreement by DSP under Section 15.3, as of the effective date of such termination all relevant licenses and sublicenses granted by
Intercept to DSP shall cease and all such licenses and sublicenses shall revert in full to Intercept. If there is a partial termination, only the
licenses and sublicenses as to the respective country and/or indication being terminated shall revert to Intercept. In order to revert the
licenses and sublicenses, DSP shall be obligated to the following:

(a)          DSP shall provide to Intercept (or at Intercept’s request, destroy) all remaining Product and
disclose to Intercept all material research, non-clinical and clinical data on Products generated prior to the termination date and Intercept
shall thereafter have the unrestricted right to use such data and information;

assignment is permitted by applicable Regulatory Authorities; and

(b)          DSP shall assign to Intercept all Regulatory Filings relating to Products in the Territory, if

(c)          DSP shall promptly provide to Intercept any other material, reagents, information, contracts,
etc.  DSP  owns  or  Controls  related  to  the  Intercept  Product  and  are  reasonably  required  to  allow  Intercept  to  continue  the  research,
Development, protection, and Commercialization of Products with minimal delay.

this Section 15 are in addition to any other relief and remedies available to either Party at law.

15.4.3      Remedies. Except as otherwise expressly set forth in this Agreement, the termination provisions of

upon any termination or expiration of the agreement.

15.4.4      Joint Improvements. For the avoidance of doubt, Joint Improvements shall remain jointly owned

15.4.5            Surviving  Provisions.  Notwithstanding  any  provision  herein  to  the  contrary,  the  rights  and
obligations  of  the  Parties  set  forth  in  Sections  10.3,  11.1,  12,  14,  and  15.4  shall  survive  the  date  of  termination  or  expiration  of  the
Agreement (except as otherwise provided for in this Agreement). Without limiting the generality of the foregoing, DSP shall have no
obligation to make any milestone or royalty payment to Intercept that has not accrued prior to the effective date of any termination or
expiration  of  this  Agreement  (except  with  respect  to  the  payments  pursuant  to  Section  15.4.1),  but  shall  remain  liable  for  all  such
payment obligations accruing prior to the effective date of such termination.

39

16.         DISPUTES

16.1         Executive Negotiation. The Parties recognize that a bona fide dispute as to certain matters may from time to
time  arise  during  the  Term  of  this  Agreement  that  relates  to  either  Party’s  rights  and/or  obligations  hereunder.  In  the  event  of  the
occurrence of such a dispute, either Party may, by written notice to the other Party, have such dispute referred to their respective senior
officials designated below or their successors, for attempted resolution by good faith negotiations within sixty (60) days after such notice
is received. Said designated senior officials are as follows:

For Intercept: Chief Executive Officer

For DSP: Chief Executive Officer (or a designated senior executive with decision-making authority).

In the event the designated senior officials are not able to resolve such dispute within the sixty (60) day period, either Party may

invoke the provisions of Section 16.2.

16.2         Arbitration. Subject to Section 16.1 and except with respect to disputes relating to the intellectual property
or a breach of the confidentiality obligations of this Agreement, any dispute, controversy or claim initiated by either Party arising out of,
resulting from or relating to this Agreement, or the performance by either Party of its obligations under this Agreement (other than bona
fide Third Party actions or proceedings filed or instituted in an action or proceeding by a Third Party against a Party), whether before or
after  termination  of  this  Agreement,  shall  be  submitted  to  the  International  Court  of  Arbitration  of  the  International  Chamber  of
Commerce and shall be finally settled by binding arbitration. Whenever a Party shall decide to institute arbitration proceedings, it shall
give written notice to that effect to the other Party. Any such arbitration shall be conducted under the then-current Rules of Arbitration of
the International Chamber of Commerce Rules of Arbitration by a panel of one or more arbitrators appointed in accordance with such
rules. Any such arbitration shall be held in New York, New York if initiated by DSP and in Osaka, Japan if initiated by Intercept. All
arbitration proceedings, communications, and documents shall be in the English language. Judgment upon the award so rendered may be
entered in any court having jurisdiction or application may be made to such court for judicial acceptance of any award and an order of
enforcement,  as  the  case  may  be.  Notwithstanding  the  foregoing,  each  Party  may  at  any  time  pursue  equitable  remedies,  including
without limitation injunctive relief, to protect its respective Confidential Information as well as its respective intellectual property rights,
including Know-How and Patents.  For the avoidance of doubt, either Party can take such action without first having to go to the JSC
pursuant to Section 3, or the Executive Negotiation pursuant to Section 16.1.

40

17.         MISCELLANEOUS

17.1                  Notification.  All  notices,  requests  and  other  communications  hereunder  shall  be  in  writing,  shall  be
addressed to the receiving Party’s address set forth below or to such other address as a Party may designate by notice hereunder, and shall
be either (i) delivered by hand, (ii) made by facsimile transmission (to be followed with written fax confirmation), (iii) sent by private
courier service providing evidence of receipt, or (iv) sent by registered or certified mail, return receipt requested, postage prepaid. The
addresses and other contact information for the parties are as follows:

If to Intercept:

If to DSP:

Intercept Pharmaceuticals, Inc.
18 Desbrosses Street
New York, NY 10013
Fax: +1-646-747-1001

Director of Business Development
6-8, Doshomachi 2-Chome
Chuo-ku, Osaka 541-0045, Japan
Fax: +81-6-6203-4533

All notices, requests and other communications hereunder shall be deemed to have been given either (i) if by hand, at the time of the
delivery thereof to the receiving Party at the address of such Party set forth above, (ii) if made by telecopy or facsimile transmission, at
the time that receipt thereof has been acknowledged by the recipient, (iii) if sent by private courier, on the day such notice is delivered to
the recipient, or (iv) if sent by registered or certified mail, on the fifth (5th ) business day following the day such mailing is made.

17.2         Governing Law. This Agreement will be construed, interpreted and applied in accordance with the laws of

the state of New York (excluding its conflict of law principles law).

or license to any of its intellectual property.

17.3         Limitations. Except as expressly set forth in this Agreement, neither Party grants to the other Party any right

17.4         Entire Agreement. This is the entire Agreement between the Parties with respect to the subject matter hereof
and supersedes all prior representations, understandings and agreements between the Parties with respect to the subject matter hereof. No
modification shall be effective unless in writing with specific reference to this Agreement and signed by the Parties.

17.5         Waiver. The terms or conditions of this Agreement may be waived only by a written instrument executed by
the Party waiving compliance. The failure of either Party at any time or times to require performance of any provision hereof shall in no
manner  affect  its  rights  at  a  later  time  to  enforce  the  same.  No  waiver  by  either  Party  of  any  condition  or  term  shall  be  deemed  as  a
continuing waiver of such condition or term or of another condition or term.

17.6         Assignment. Neither this Agreement nor any right or obligation hereunder may be assigned, delegated or
otherwise  transferred,  in  whole  or  part,  by  either  Party  without  the  prior  express  written  consent  of  the  other  Party,  which  may  be
withheld in the sole discretion of the Party giving such consent.

41

 
 
17.7         Force Majeure. Neither Party shall be liable for failure of or delay in performing obligations set forth in this
Agreement,  and  neither  shall  be  deemed  in  breach  of  its  obligations,  if  such  failure  or  delay  is  due  to  natural  disasters  or  any  cause
beyond the reasonable control of such Party. In event of such force majeure, the Party affected thereby shall use reasonable efforts to cure
or overcome the same and resume performance of its obligations hereunder.

17.8         Construction. The Parties hereto acknowledge and agree that: (i) each Party and its counsel reviewed and
negotiated the terms and provisions of this Agreement and have contributed to its revision; (ii) the rule of construction to the effect that
any ambiguities are resolved against the drafting Party shall not be employed in the interpretation of this Agreement; and (iii) the terms
and provisions of this Agreement shall be construed fairly as to all Parties hereto and not in favor of or against any Party, regardless of
which Party was generally responsible for the preparation of this Agreement.

17.9         Severability. If any provision(s) of this Agreement are or become invalid, are ruled illegal by any court of
competent jurisdiction or are deemed unenforceable under then current applicable law from time to time in effect during the Term hereof,
it is the intention of the Parties that the remainder of this Agreement shall not be affected thereby provided that a Party’s rights under this
Agreement  are  not  materially  affected.  The  Parties  hereto  covenant  and  agree  to  renegotiate  any  such  term,  covenant  or  application
thereof in good faith in order to provide a reasonably acceptable alternative to the term, covenant or condition of this Agreement or the
application thereof that is invalid, illegal or unenforceable, it being the intent of the Parties that the basic purposes of this Agreement are
to be effectuated.

to do all such other acts, as may be necessary or appropriate in order to carry out the purposes and intent of this Agreement.

17.10         Further Assurances. Each Party agrees to execute, acknowledge and deliver such further instructions, and

it shall provide prior notice to Intercept.

17.11         Affiliate Delegation. DSP may delegate to an Affiliate all or part of its obligations hereunder, provided that

17.12          Compliance with Law. Each Party shall comply with all applicable Laws, including by way of example,

but without limitation U.S. export controls and the U.S. Foreign Corrupt Practices Act.

17.13         Governing Language. This Agreement has been executed in English. If any translation of this Agreement
conflicts with the English version or contains terms in addition to or different from the English version, the English version shall prevail.

which shall be deemed an original, but all of which together shall constitute one and the same instrument.

17.14                  Counterparts.  This  Agreement  may  be  executed  simultaneously  in  one  or  more  counterparts,  each  of

42

[SIGNATURES FOLLOW ON THE NEXT PAGE.]

43

IN WITNESS WHEREOF, the Parties have caused this Agreement to be executed by their duly authorized representative in

two (2) originals.

DAINIPPON SUMITOMO PHARMA CO., LTD.

INTERCEPT PHARMACEUTICALS, INC.

/s/ Masayo Tada

Name: Masayo Tada

/s/ Mark Pruzanski

  Name: Mark Pruzanski

Title: President and Chief Executive Officer

  Title: President and Chief Executive Officer

44

 
 
 
 
 
 
 
 
 
 
 
EXHIBIT A

INTERCEPT PATENTS

Country Title
Japan

Steroids As Agonists For FXR

Serial No.
2002-571512

Filing
Date
Feb. 21,
2002

Parent PCT
PCT/EP2002/001832
WO2002/072598

Patent
No.

Status
Granted 4021327

Japan

 Process For Preparing 3alpha(Beta)-7alpha(Beta)-
Dihydroxy-6alpha(Beta)-Alkyl-5beta Cholanic Acid

 2008-511719

  May 19,
2006

 PCT/EP2006/062446
WO2006/122977

  Pending  N/A

China

 Process For Preparing 3alpha(Beta)-7alpha(Beta)-
Dihydroxy-6alpha(Beta)-Alkyl-5beta Cholanic Acid

 200680017025.6   May 19,

2006

 PCT/EP2006/062446
WO2006/122977

  Pending  N/A

Japan

 Treatment Of Fibrosis Using FXR Ligands

 2007-503111

  Mar. 14,
2005

 PCT/US2005/008575
WO2005/089316

  Pending  N/A

45

 
  
  
   
  
   
  
 
  
  
   
  
   
  
EXHIBIT B

Summary of Sublicense Agreements

1. Sublicense Agreement

(a) Full corporate name of sublicensee:

(b) Applicable country:

(c) Applicable indications in the Field:

(d) Standard of sublicensee’s performance (e.g. best efforts, commercially reasonable efforts, etc.):

(e) Term of sublicense agreement:

(f) Summary of termination provision:

2. Sublicensee Confirmation

I, [Name], the [Title] of [Full Corporate Name of Sublicensee] (the “XX”) confirm and acknowledge that the XX is aware of and
agrees to comply with the provisions of that certain License Agreement, dated March 29, 2011 by and between Dainippon Sumitomo
Pharma Co., Ltd. and Intercept Pharmaceuticals, Inc. (the “Agreement”), which in accordance with their respective terms, are expressly
applicable to XX, as a sublicensee appointed pursuant to Section 2.1.2 of the Agreement.

By:

Name:

Title:

Date:

46

SUBSIDIARIES OF THE REGISTRANT

Exhibit 21.1

Name

Jurisdiction of Incorporation or Organization

Intercept Pharma International Limited
Intercept Pharmaceuticals, LLC
Intercept Italia S.r.l.
Intercept Pharma Europe Ltd.
Intercept Pharma UK & Ireland Ltd
Intercept Pharma Ltd
Intercept Pharma Canada Inc.
Intercept Pharma Switzerland GmbH
Intercept Pharma Deutschland GmbH
Intercept Pharma France SAS
Intercept Pharma Austria GmbH
Intercept Pharma Spain, S.L.U.
Intercept Pharma Portugal Unipessoal Lda
Intercept Pharma Nederland B.V.

Republic of Ireland
Delaware
Italy
England and Wales
England and Wales
England and Wales
British Columbia
Switzerland
Germany
France
Austria
Spain
Portugal
The Netherlands

Consent of Independent Registered Public Accounting Firm

Exhibit 23.1

The Board of Directors
Intercept Pharmaceuticals, Inc.:

We consent to the incorporation by reference in the registration statements (No. 333-184810, No. 333-188064, No. 333-
206247, No. 333-217863, No. 333-226405, No. 333-233248, and No. 333-248083) on Form S-8 and (No. 333-194974 and
No. 333-217861) on Form S-3 of Intercept Pharmaceuticals, Inc. of our reports dated February 25, 2021, with respect to the
consolidated balance sheets of Intercept Pharmaceuticals, Inc. as of December 31, 2020 and 2019, the related consolidated
statements of operations, comprehensive loss, changes in stockholders’ (deficit) equity, and cash flows for each of the years
in  the  three-year  period  ended  December  31,  2020,  and  the  related  notes  and  the  effectiveness  of  internal  control  over
financial reporting as of December 31, 2020, which reports appear in the December 31, 2020 annual report on Form 10-K
of Intercept Pharmaceuticals, Inc.

/s/ KPMG LLP

New York, New York
February 25, 2021

I, Jerome Durso, certify that:

CERTIFICATION

Exhibit 31.1

1.    I have reviewed this Annual Report on Form 10-K of Intercept Pharmaceuticals, Inc.;

2.    Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material fact necessary to make the statements made, in light of the circumstances under which such statements
were made, not misleading with respect to the period covered by this report;

3.    Based on my knowledge, the financial statements, and other financial information included in this report, fairly
present in all material respects the financial condition, results of operations and cash flows of the registrant as of,
and for, the periods presented in this report;

4.        The  registrant’s  other  certifying  officer(s)  and  I  are  responsible  for  establishing  and  maintaining  disclosure
controls  and  procedures  (as  defined  in  Exchange  Act  Rules  13a-15(e)  and  15d-15(e))  and  internal  control  over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

a)    Designed such disclosure controls and procedures, or caused such disclosure controls and procedures to be
designed  under  our  supervision,  to  ensure  that  material  information  relating  to  the  registrant,  including  its
consolidated subsidiaries, is made known to us by others within those entities, particularly during the period
in which this report is being prepared;

b)        Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over  financial
reporting to be designed under our supervision, to provide reasonable assurance regarding the reliability of
financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles;

c)    Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in this report
our conclusions about the effectiveness of the disclosure controls and procedures, as of the end of the period
covered by this report based on such evaluation; and

d)    Disclosed in this report any change in the registrant's internal control over financial reporting that occurred
during the registrant's most recent fiscal quarter (the registrant's fourth fiscal quarter in the case of an annual
report) that has materially affected, or is reasonably likely to materially affect, the registrant's internal control
over financial reporting; and

5.    The registrant’s other certifying officer(s) and I have disclosed, based on our most recent evaluation of internal
control  over  financial  reporting,  to  the  registrant’s  auditors  and  the  audit  committee  of  the  registrant’s  board  of
directors (or persons performing the equivalent functions):

a)        All  significant  deficiencies  and  material  weaknesses  in  the  design  or  operation  of  internal  control  over
financial reporting which are reasonably likely to adversely affect the registrant’s ability to record, process,
summarize and report financial information; and

b)    Any fraud, whether or not material, that involves management or other employees who have a significant role

in the registrant’s internal control over financial reporting.

Date: February 25, 2021

/s/ Jerome Durso
Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

I, Sandip Kapadia, certify that:

CERTIFICATION

Exhibit 31.2

1.    I have reviewed this Annual Report on Form 10-K of Intercept Pharmaceuticals, Inc.;

2.    Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material fact necessary to make the statements made, in light of the circumstances under which such statements
were made, not misleading with respect to the period covered by this report;

3.    Based on my knowledge, the financial statements, and other financial information included in this report, fairly
present in all material respects the financial condition, results of operations and cash flows of the registrant as of,
and for, the periods presented in this report;

4.        The  registrant’s  other  certifying  officer(s)  and  I  are  responsible  for  establishing  and  maintaining  disclosure
controls  and  procedures  (as  defined  in  Exchange  Act  Rules  13a-15(e)  and  15d-15(e))  and  internal  control  over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

a)    Designed such disclosure controls and procedures, or caused such disclosure controls and procedures to be
designed  under  our  supervision,  to  ensure  that  material  information  relating  to  the  registrant,  including  its
consolidated subsidiaries, is made known to us by others within those entities, particularly during the period
in which this report is being prepared;

b)        Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over  financial
reporting to be designed under our supervision, to provide reasonable assurance regarding the reliability of
financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles;

c)    Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in this report
our conclusions about the effectiveness of the disclosure controls and procedures, as of the end of the period
covered by this report based on such evaluation; and

d)    Disclosed in this report any change in the registrant's internal control over financial reporting that occurred
during the registrant's most recent fiscal quarter (the registrant's fourth fiscal quarter in the case of an annual
report) that has materially affected, or is reasonably likely to materially affect, the registrant's internal control
over financial reporting; and

5.    The registrant’s other certifying officer(s) and I have disclosed, based on our most recent evaluation of internal
control  over  financial  reporting,  to  the  registrant’s  auditors  and  the  audit  committee  of  the  registrant’s  board  of
directors (or persons performing the equivalent functions):

a)        All  significant  deficiencies  and  material  weaknesses  in  the  design  or  operation  of  internal  control  over
financial reporting which are reasonably likely to adversely affect the registrant’s ability to record, process,
summarize and report financial information; and

b)    Any fraud, whether or not material, that involves management or other employees who have a significant role

in the registrant’s internal control over financial reporting.

Date: February 25, 2021

/s/ Sandip Kapadia
Sandip Kapadia
Chief Financial Officer and Treasurer
(Principal Financial Officer)

CERTIFICATION

Exhibit 32.1

Pursuant  to  the  requirement  set  forth  in  Rule  13a-14(b)  of  the  Securities  Exchange  Act  of  1934,  as  amended  (the
“Exchange Act”), and Section 1350 of Chapter 63 of Title 18 of the United States Code (18 U.S.C. §1350), Jerome Durso,
President  and  Chief  Executive  Officer  of  Intercept  Pharmaceuticals,  Inc.  (the  “Company”),  and  Sandip  Kapadia,  Chief
Financial Officer and Treasurer of the Company, each hereby certifies that, to the best of his knowledge:

(1) The Company’s Annual Report on Form 10-K for the year ended December 31, 2020 to which this Certification is
attached as Exhibit 32.1 (the “Periodic Report”), fully complies with the requirements of Section 13(a) or Section
15(d) of the Exchange Act; and

(2) The information contained in the Periodic Report fairly presents, in all material respects, the financial condition

and results of operations of the Company.

Dated: February 25, 2021

Dated: February 25, 2021

/s/ Jerome Durso
Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

/s/ Sandip Kapadia
Sandip Kapadia
Chief Financial Officer and Treasurer
(Principal Financial Officer)

A  signed  original  of  this  written  statement  required  by  Rule  13a-14(b)  of  the  Exchange  Act  and  Section  1350  of
Chapter 63 of Title 18 of the United States Code (18 U.S.C. §1350) has been provided to Intercept Pharmaceuticals, Inc.
and  will  be  retained  by  Intercept  Pharmaceuticals,  Inc.  and  furnished  to  the  Securities  and  Exchange  Commission  or  its
staff upon request.

This  certification  accompanies  the  Annual  Report  on  Form  10-K  to  which  it  relates,  is  not  deemed  filed  with  the
Securities  and  Exchange  Commission  and  is  not  to  be  incorporated  by  reference  into  any  filing  of  Intercept
Pharmaceuticals, Inc. under the Securities Act of 1933, as amended, or the Exchange Act (whether made before or after the
date of the Annual Report on Form 10-K), irrespective of any general incorporation language contained in such filing.