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Intercept Pharmaceuticals

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FY2021 Annual Report · Intercept Pharmaceuticals
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UNITED STATES
SECURITIES AND EXCHANGE COMMISSION
WASHINGTON, D.C. 20549

FORM 10-K

(Mark One)

☒   ANNUAL REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the fiscal year ended December 31, 2021

OR

☐   TRANSITION REPORT PURSUANT TO SECTION 13 OR 15(d) OF THE SECURITIES EXCHANGE ACT OF 1934

For the transition period from             to

Commission file number: 001-35668

Intercept Pharmaceuticals, Inc.
(Exact Name of Registrant as Specified in Its Charter)

Delaware
(State or Other Jurisdiction of
Incorporation or Organization)

22-3868459
(I.R.S. Employer
Identification No.)

10 Hudson Yards, 37th Floor
New York, NY 10001
(Address of Principal Executive Offices and Zip Code)
(646) 747-1000
(Registrant’s Telephone Number, Including Area Code)

Securities registered pursuant to Section 12(b) of the Act:

Title of each class

Common Stock, par value $0.001 per share

Trading Symbol(s)

ICPT

Name of each exchange on which registered

Nasdaq Global Select Market

Securities registered pursuant to Section 12(g) of the Act: None

Indicate by check mark if the registrant is a well-known seasoned issuer, as defined in Rule 405 of the Securities Act. Yes ☐ No ☒

Indicate by check mark if the registrant is not required to file reports pursuant to Section 13 or Section 15(d) of the Act. Yes ☐ No ☒

Indicate  by  check  mark  whether  the  registrant  (1)  has  filed  all  reports  required  to  be  filed  by  Section  13  or  15(d)  of  the  Securities  Exchange  Act  of  1934  during  the
preceding 12 months (or for such shorter period that the registrant was required to file such reports), and (2) has been subject to such filing requirements for the past 90 days. Yes
☒ No ☐

Indicate by check mark whether the registrant has submitted electronically every Interactive Data File required to be submitted pursuant to Rule 405 of Regulation S-T (§

232.405 of this chapter) during the preceding 12 months (or for such shorter period that the registrant was required to submit such files).Yes ☒ No ☐

Indicate by check mark whether the registrant is a large accelerated filer, an accelerated filer, a non-accelerated filer, a smaller reporting company, or an emerging growth

company. See the definitions of “large accelerated filer,” “accelerated filer,” “smaller reporting company,” and “emerging growth company” in Rule 12b-2 of the Exchange Act:

       Large accelerated filer
       Non-accelerated filer

☐
☐

Accelerated filer
Smaller reporting company
Emerging growth company

☒
☐
☐

If  an  emerging  growth  company,  indicate  by  check  mark  if  the  registrant  has  elected  not  to  use  the  extended  transition  period  for  complying  with  any  new  or  revised

financial accounting standards provided pursuant to Section 13(a) of the Exchange Act. ☐

Indicate by check mark whether the registrant has filed a report on and attestation to its management’s assessment of the effectiveness of its internal control over financial

reporting under Section 404(b) of the Sarbanes-Oxley Act (15 U.S.C. 7262(b)) by the registered public accounting firm that prepared or issued its audit report. ☒

Indicate by check mark whether the registrant is a shell company (as defined in Rule 12b-2 of the Act).Yes ☐ No ☒

The aggregate market value of the registrant’s common stock held by non-affiliates as of June 30, 2021, the last business day of the registrant’s most recently completed
second fiscal quarter, was $555.2 million (computed by reference to the closing price of $19.97 on such date as reported by the Nasdaq Global Select Market). Common stock
held by our executive officers, directors and certain stockholders as of such date has been excluded from this calculation because such persons may be deemed to be affiliates.
This determination of affiliate status is not necessarily a conclusive determination for other purposes.

The number of shares of the registrant’s common stock outstanding as of January 31, 2022 was 29,692,592.

DOCUMENTS INCORPORATED BY REFERENCE
Certain information required by Part III of this Annual Report on Form 10-K is incorporated by reference to the registrant’s definitive proxy statement related to its 2022

Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the fiscal year covered by this Annual Report on Form 10-K.

    
Intercept Pharmaceuticals, Inc.
Annual Report on Form 10-K
For the Fiscal Year Ended December 31, 2021

TABLE OF CONTENTS

Part I.

Business

Item 1.
Item 1A. Risk Factors
Item 1B. Unresolved Staff Comments
Item 2.
Item 3.
Item 4. Mine Safety Disclosures

Properties
Legal Proceedings

Part II.

Item 5. Market for Registrant’s Common Equity, Related Stockholder Matters and Issuer Purchases of Equity

Securities
Reserved

Item 6.
Item 7. Management’s Discussion and Analysis of Financial Condition and Results of Operations
Item 7A. Quantitative and Qualitative Disclosures About Market Risk
Item 8.
Item 9.
Item 9A. Controls and Procedures
Item 9B. Other Information
Item 9C. Disclosure Regarding Foreign Jurisdictions that Prevent Inspections

Financial Statements and Supplementary Data
Changes in and Disagreements With Accountants on Accounting and Financial Disclosure

Part III.

Item 10. Directors, Executive Officers and Corporate Governance
Item 11. Executive Compensation
Item 12. Security Ownership of Certain Beneficial Owners and Management and Related Stockholder Matters
Item 13. Certain Relationships and Related Transactions, and Director Independence
Item 14. Principal Accounting Fees and Services

Part IV.

Item 15. Exhibits and Financial Statement Schedules
Item 16. Form 10-K Summary
Signatures

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Unless the context otherwise requires, references in this Annual Report on Form 10-K to “we,” “our,” “us” and the
“Company” refer, collectively, to Intercept Pharmaceuticals, Inc., a Delaware corporation, and its consolidated subsidiaries.

i

CAUTIONARY NOTE REGARDING FORWARD-LOOKING STATEMENTS

This  Annual  Report  on  Form  10-K  contains  forward-looking  statements,  including,  but  not  limited  to,  statements
regarding the progress, timing and results of our clinical trials, including our clinical trials for the treatment of nonalcoholic
steatohepatitis  (“NASH”),  the  safety  and  efficacy  of  our  approved  product,  Ocaliva  (obeticholic  acid  or  “OCA”)  for
primary biliary cholangitis (“PBC”), and our product candidates, including OCA for liver fibrosis due to NASH, the timing
and acceptance of our regulatory filings and the potential approval of OCA for liver fibrosis due to NASH, the review of
our  New  Drug  Application  for  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH  by  the  U.S.  Food  and  Drug
Administration  (the  “FDA”),  our  intent  to  work  with  the  FDA  to  address  the  issues  raised  in  a  complete  response  letter
(“CRL”),  the  potential  commercial  success  of  OCA,  as  well  as  our  strategy,  future  operations,  future  financial  position,
future revenue, projected costs, financial guidance, prospects, plans and objectives.

These  statements  constitute  forward-looking  statements  within  the  meaning  of  Section  27A  of  the  Securities  Act  of
1933,  as  amended,  and  Section  21E  of  the  Securities  Exchange  Act  of  1934,  as  amended.  The  words  “anticipate,”
“believe,”  “estimate,”  “expect,”  “intend,”  “may,”  “plan,”  “predict,”  “project,”  “target,”  “potential,”  “will,”  “would,”
“could,”  “should,”  “possible,”  “continue”  and  similar  expressions  are  intended  to  identify  forward-looking  statements,
although  not  all  forward-looking  statements  contain  these  identifying  words.  Readers  are  cautioned  not  to  place  undue
reliance on these forward-looking statements, which speak only as of their dates, and we undertake no obligation to update
any  forward-looking  statement  except  as  required  by  law.  These  forward-looking  statements  are  based  on  estimates  and
assumptions by our management that, although believed to be reasonable, are inherently uncertain and subject to a number
of risks.

The following represent some, but not necessarily all, of the factors that could cause actual results to differ materially

from historical results or those anticipated or predicted by our forward-looking statements:

● our ability to successfully commercialize Ocaliva for PBC;

● our  ability  to  maintain  our  regulatory  approval  of  Ocaliva  for  PBC  in  the  United  States,  Europe,  Canada,  Israel,

Australia and other jurisdictions in which we have or may receive marketing authorization;

● our  ability  to  timely  and  cost-effectively  file  for  and  obtain  regulatory  approval  of  our  product  candidates  on  an
accelerated basis or at all, including OCA for liver fibrosis due to NASH following the issuance of the CRL by the
FDA;  any  advisory  committee  recommendation  or  dispute  resolution  determination  that  our  product  candidates,
including OCA for liver fibrosis due to NASH, should not be approved or approved only under certain conditions; or
any  future  determination  that  the  regulatory  applications  and  subsequent  information  we  submit  for  our  product
candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  do  not  contain  adequate  clinical  or  other  data  or  meet
applicable regulatory requirements for approval;

● conditions  that  may  be  imposed  by  regulatory  authorities  on  our  marketing  approvals  for  our  products  and  product
candidates, including OCA for liver fibrosis due to NASH, such as the need for clinical outcomes data (and not just
results  based  on  achievement  of  a  surrogate  endpoint),  any  risk  mitigation  programs  such  as  a  Risk  Evaluation  and
Mitigation  Strategies  (“REMS”)  program,  and  any  related  restrictions,  limitations  and/or  warnings  contained  in  the
label of any of our products or product candidates;

● any potential side effects associated with Ocaliva for PBC, OCA for liver fibrosis due to NASH or our other product
candidates that could delay or prevent approval, require that an approved product be taken off the market, require the
inclusion of safety warnings or precautions, or otherwise limit the sale of such product or product candidate, including
in  connection  with  our  update  to  the  Ocaliva  prescribing  information  in  May  2021  contraindicating  Ocaliva  for
patients  with  PBC  and  decompensated  cirrhosis,  a  prior  decompensation  event,  or  compensated  cirrhosis  with
evidence of portal hypertension;

● the initiation, timing, cost, conduct, progress and results of our research and development activities, preclinical studies
and clinical trials, including any issues, delays or failures in identifying patients, enrolling patients, treating patients,
retaining patients, meeting specific endpoints in the jurisdictions in which we intend to seek approval or completing
and timely reporting the results of our NASH or PBC clinical trials;

● the outcomes of interactions with regulators (e.g., the FDA and the European Medicines Agency ("EMA")) regarding

our clinical trials;

ii

● our  ability  to  establish  and  maintain  relationships  with,  and  the  performance  of,  third-party  manufacturers,  contract
research  organizations  and  other  vendors  upon  whom  we  are  substantially  dependent  for,  among  other  things,  the
manufacture and supply of our products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to
NASH, and our clinical trial activities;

● our  ability  to  identify,  develop  and  successfully  commercialize  our  products  and  product  candidates,  including  our

ability to successfully launch OCA for liver fibrosis due to NASH, if approved;

● our ability to obtain and maintain intellectual property protection for our products and product candidates, including
our ability to cost-effectively file, prosecute, defend and enforce any patent claims or other intellectual property rights;

● the size and growth of the markets for our products and product candidates and our ability to serve those markets;

● the  degree  of  market  acceptance  of  Ocaliva  for  PBC  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH  or  our

other product candidates among physicians, patients and healthcare payors;

● the  availability  of  adequate  coverage  and  reimbursement  from  governmental  and  private  healthcare  payors  for  our
products, including Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH, and our ability to obtain
adequate pricing for such products;

● our ability to establish and maintain effective sales, marketing and distribution capabilities, either directly or through

collaborations with third parties;

● competition from existing drugs or new drugs that become available;

● our ability to attract and retain key personnel to manage our business effectively;

● our  ability  to  prevent  or  defend  against  system  failures  or  security  or  data  breaches  due  to  cyber-attacks,  or  cyber

intrusions, including ransomware, phishing attacks and other malicious intrusions;

● our ability to comply with data protection laws;

● costs  and  outcomes  relating  to  any  disputes,  governmental  inquiries  or  investigations,  regulatory  proceedings,  legal
proceedings  or  litigation,  including  any  securities,  intellectual  property,  employment,  product  liability  or  other
litigation;

● our collaborators’ election to pursue research, development and commercialization activities;

● our  ability 

to  establish  and  maintain  relationships  with  collaborators  with  development,  regulatory  and

commercialization expertise;

● our need for and ability to generate or obtain additional financing;

● our estimates regarding future expenses, revenues and capital requirements and the accuracy thereof;

● our use of cash, cash equivalents and short-term investments;

● our ability to acquire, license and invest in businesses, technologies, product candidates and products;

● our ability to manage the growth of our operations, infrastructure, personnel, systems and controls;

● our ability to obtain and maintain adequate insurance coverage;

● continuing threats from COVID-19, including additional waves of infections, and their impacts including quarantines
and  other  government  actions;  delays  relating  to  our  regulatory  applications;  disruptions  relating  to  our  ongoing
clinical trials or involving our contract research organizations, study sites or other clinical partners; disruptions relating
to our supply chain or involving our third-party manufacturers, distributors or other distribution partners; and facility
closures or other restrictions; and the impact of the foregoing on our results of operations and financial position;

● the  impact  of  general  U.S.  and  foreign  economic,  industry,  market,  regulatory  or  political  conditions,  including  the

impact of Brexit; and

the  other  risks  and  uncertainties  identified  under  the  captions  “Risk  Factors”  and  “Management’s  Discussion  and
Analysis of Financial Condition and Results of Operations” and elsewhere in this Annual Report on Form 10-K and in
our other periodic filings filed with the U.S. Securities and Exchange Commission (the “SEC”).

iii

NOTE REGARDING TRADEMARKS

The Intercept Pharmaceuticals® name and logo and the Ocaliva® name and logo are either registered or unregistered
trademarks or trade names of the Company in the United States and/or other countries. All other trademarks, trade names
and service marks appearing in this Annual Report on Form 10-K are the property of their respective owners. Solely for
convenience, trademarks and trade names referred to in this Annual Report on Form 10-K may appear without the ® and
™ symbols, but those references are not intended to indicate, in any way, that we will not assert, to the fullest extent under
applicable law, our rights or that the applicable owner will not assert its rights to these trademarks and trade names.

iv

SUMMARY RISK FACTORS

Investing in our securities involves a high degree of risk. Investors should carefully consider the risks and uncertainties
discussed under the caption “Risk Factors” and elsewhere in this Annual Report on Form 10-K before deciding whether to
invest in our securities. The following is a list of some of these risks:

Risks Related to Our Financial Position and Need for Additional Capital

● We  are  currently  dependent  on  the  successful  commercialization  of  Ocaliva  for  PBC.  To  the  extent  Ocaliva  is  not
commercially successful, our business, financial condition and results of operations may be materially and adversely
affected and the price of our common stock may decline.

● We have never been profitable. We expect to incur losses for the foreseeable future, and we may never achieve or

sustain profitability.

● We  will  require  substantial  additional  funding,  which  may  not  be  available  to  us  on  acceptable  terms,  if  at  all.  If

adequate funds are not available to us, we may be required to delay, limit, reduce or cease our operations.

● Raising additional capital may cause dilution to our stockholders, restrict our operations or require us to relinquish

rights to our technologies or product candidates.

Risks Related to the Development and the Regulatory Review and
Approval of Our Products and Product Candidates

● We  cannot  be  certain  whether  Ocaliva  will  receive  full  approval  for  PBC  in  jurisdictions  where  it  has  previously
received accelerated or conditional approval, or that Ocaliva will be approved for PBC in any jurisdictions beyond
those in which it is currently approved. Furthermore, OCA may not be approved on an accelerated basis, or at all, for
NASH  or  any  other  indication  beyond  PBC  and  we  may  not  receive  regulatory  approval  for  any  other  product
candidate. Without regulatory approval, we will not be able to market and commercialize our product candidates.

● We are developing product candidates for the treatment of rare diseases or diseases for which there are no or limited
therapies, such as PBC and NASH, and for some of which there is little clinical experience, and our development
approach involves new endpoints and methodologies. As a result, there is a heightened risk that we will not be able to
gain  agreement  with  regulatory  authorities  regarding  an  acceptable  development  plan,  that  the  outcome  of  our
clinical trials will not be favorable or that, even if favorable, regulatory authorities may not find the results of our
clinical trials to be sufficient for marketing approval.

● Delays  or  difficulties  in  the  commencement,  enrollment  and  completion  of  our  clinical  trials  and  studies  could
increase our product development costs and delay, limit or prevent us from obtaining regulatory approval for OCA
and our other product candidates.

● Continuing threats from COVID-19, including additional waves of infections, could materially and adversely affect

our clinical trials.

● Failure  can  occur  at  any  stage  of  clinical  development.  The  results  of  earlier  clinical  trials  are  not  necessarily
predictive  of  future  results  and  any  product  candidate  we  or  our  collaborators  advance  through  clinical  trials,
including OCA, may not have favorable results in later clinical trials or receive or maintain regulatory approval.

● Our  product  candidates  may  have  undesirable  side  effects  which  may  delay  or  prevent  marketing  approval,  or,  if
approval is received, require that our products be taken off the market or include new or additional safety warnings.
Any  such  events  may  limit  our  existing  and  future  product  sales  and  materially  and  adversely  affect  our  business,
financial condition and results of operations.

● We may not be able to obtain or, if approved, maintain orphan drug exclusivity for our approved products or product

candidates, which could cause our revenues to suffer.

Risks Related to the Commercialization of Our Products

● Sales of Ocaliva may be adversely affected by safety and labeling changes required by regulators.

● We are subject to uncertainty relating to pricing and reimbursement. Failure to obtain or maintain adequate coverage,
pricing and reimbursement for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future
approved products, if any, could have a material adverse impact on our ability to commercialize such products.

v

● Legislative and regulatory healthcare reform may adversely affect our business.

● Ocaliva and our other future approved products, if any, may not achieve broad market acceptance among physicians,

patients and healthcare payors, and revenues generated from their sales may be limited as a result.

● If we fail to develop OCA for additional indications such as NASH, our commercial opportunity will be limited.

Risks Related to Our Business and Strategy

● We depend on third-party contractors for a substantial portion of our operations and may not be able to control their

work as effectively as if we performed these functions ourselves.

● We face rapid technological change and competition from other biotechnology and pharmaceutical companies. Our

operating results will suffer if we fail to compete effectively.

● Our business and operations would suffer in the event of system failures or security or data breaches due to cyber-

attacks, or cyber intrusions, including ransomware, phishing attacks and other malicious intrusions.

● We are subject to various data protection laws and our business and operations would suffer in the event of violations

of these laws.

Risks Related to Our Intellectual Property

● It is difficult and costly to protect our proprietary rights, and we may not be able to ensure their protection. If our
patent  position  does  not  adequately  protect  our  products  such  as  Ocaliva  and  product  candidates  such  as  OCA  for
liver fibrosis due to NASH, others may compete against us more directly, which could harm our business, possibly
materially.

● If we do not obtain protection under the Hatch-Waxman Act in the United States (and similar legislation outside of
the United States) extending the terms of our patents and/or providing data or other exclusivity for our products and
product candidates, our business may be materially harmed.

● We may incur substantial costs as a result of litigation or other proceedings relating to patent and other intellectual
property  rights,  and  such  litigation  may  divert  the  attention  of  our  management  and  scientific  personnel  and
adversely affect our development and commercialization efforts.

Risks Related to Our Indebtedness

● Servicing  our  debt  will  require  significant  amounts  of  cash,  and  we  may  not  have  sufficient  cash  flow  from  our

business to effectively service our debt.

● We may incur substantially more debt or take other actions that would affect our ability to pay the principal of and

interest on our debt.

Risks Related to Ownership of Our Common Stock

● We have previously been, and are currently, subject to securities class action litigation and may be subject to similar
or other litigation in the future. Such matters can be expensive, time-consuming and have a material adverse effect on
our business, results of operations and financial condition.

● Our stock price has been and may in the future be volatile, which could cause holders of our common stock to incur

substantial losses.

vi

Table of Contents

Item 1.   Business

Overview

PART I

We are a biopharmaceutical company focused on the development and commercialization of novel therapeutics to treat
progressive non-viral liver diseases with high unmet medical need utilizing our proprietary bile acid chemistry. Our first
marketed  product,  Ocaliva®  (obeticholic  acid  or  “OCA”),  is  a  farnesoid  X  receptor  (“FXR”)  agonist  approved  in  the
United States, the United Kingdom, the European Union and several other jurisdictions for the treatment of primary biliary
cholangitis (“PBC”) in combination with ursodeoxycholic acid (“UDCA”) in adults with an inadequate response to UDCA
or  as  monotherapy  in  adults  unable  to  tolerate  UDCA.  In  addition  to  commercializing  OCA  for  PBC  under  the  Ocaliva
brand  name,  we  are  also  currently  developing  OCA  for  additional  indications,  including  nonalcoholic  steatohepatitis
(“NASH”).  We  are  also  developing  product  candidates  in  various  stages  of  clinical  and  preclinical  development.  We
believe  that  OCA  and  our  other  product  candidates  have  the  potential  to  treat  orphan  and  other  more  prevalent  liver
diseases such as NASH for which there are currently limited therapeutic options.

Ocaliva  was  approved  for  PBC  by  the  U.S.  Food  and  Drug  Administration  (“FDA”)  in  May  2016  under  the
accelerated approval pathway. We commenced sales and marketing of Ocaliva in the United States shortly after receiving
approval,  and  Ocaliva  is  now  available  to  U.S.  patients  primarily  through  a  network  of  specialty  pharmacy  distributors.
Ocaliva received conditional approval for PBC from the European Commission in December 2016 and we commenced our
commercial  launches  across  Europe  (including  the  United  Kingdom)  in  January  2017.  We  have  submitted  dossiers  and
obtained,  or  are  otherwise  pursuing,  pricing  reimbursement  from  a  number  of  national  authorities  across  Europe.  Since
January 2017, Ocaliva has also received regulatory approval in several of our target markets outside the United States and
Europe,  including  (but  not  limited  to)  Canada,  Israel,  and  Australia,  and  we  continue  to  pursue  marketing  approval  of
Ocaliva for PBC in our other international target markets. Ocaliva has received orphan drug designation in both the United
States  and  the  European  Union  for  the  treatment  of  PBC.  In  addition,  we  continue  to  work  to  execute  on  our  post-
marketing regulatory commitments with respect to Ocaliva in the U.S. and Europe.

Our  lead  development  product  candidate  is  OCA  for  the  potential  treatment  of  NASH.  In  February  2019,  we
announced  topline  results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in
patients with liver fibrosis due to NASH, known as the REGENERATE trial. In the primary efficacy analysis, once-daily
OCA  25  mg  met  the  primary  endpoint  agreed  with  the  FDA  of  fibrosis  improvement  by  at  least  one  stage  with  no
worsening of NASH at the planned 18-month interim analysis. Adverse events were generally mild to moderate in severity
and the most common were consistent with the known profile of OCA. Interim analysis results at 18 months were based on
surrogate endpoints and the impact on clinical outcomes has not been confirmed. The REGENERATE trial is ongoing and
is expected to continue through clinical outcomes for verification and description of the clinical benefit of OCA. OCA also
achieved  the  primary  endpoint  in  a  Phase  2b  clinical  trial  for  the  treatment  of  NASH  that  completed  in  late  July  2014,
known  as  the  FLINT  trial,  which  was  sponsored  by  the  U.S.  National  Institute  of  Diabetes  and  Digestive  and  Kidney
Diseases, a part of the National Institutes of Health. OCA has received breakthrough therapy designation from the FDA for
the treatment of NASH patients with liver fibrosis.

In September 2019, we submitted a New Drug Application (“NDA”) to the FDA seeking accelerated approval of OCA
for liver fibrosis due to NASH. In November 2019, the FDA accepted our NDA for filing and granted a priority review
designation  of  OCA  for  liver  fibrosis  due  to  NASH.  In  December  2019,  we  submitted  a  Marketing  Authorization
Application  (“MAA”)  to  the  European  Medicines  Agency  (the  “EMA”)  seeking  conditional  approval  of  OCA  for  liver
fibrosis due to NASH. In January 2020, the EMA completed its technical validation of our MAA and thereby confirmed
that  all  essential  regulatory  elements  required  for  scientific  assessment  had  been  included  in  our  MAA  prior  to  the
commencement of the formal review procedure. In June 2020, we received a complete response letter (“CRL”) from the
FDA stating that our NDA for OCA for the treatment of liver fibrosis due to NASH could not be approved in its present
form. The CRL indicated that, based on the data the FDA had reviewed, the FDA has determined that the predicted benefit
of OCA based on a surrogate histopathologic endpoint remains uncertain and does not sufficiently outweigh the potential
risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH. At that time, the FDA
recommended that we submit additional post-interim analysis efficacy and safety data from the ongoing REGENERATE

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Table of Contents

trial in support of potential accelerated approval and that the long-term outcomes phase of the trial should continue. We had
our end of review meeting with the FDA in October 2020 to discuss the FDA’s risk-benefit assessment in the CRL based
on its review of the available data, as well as our proposed resubmission of our NDA for the treatment of liver fibrosis due
to NASH. The meeting was constructive and the FDA provided us with helpful guidance regarding supplemental data we
can provide to further characterize OCA’s efficacy and safety profile that could support resubmission based on our Phase 3
REGENERATE 18-month biopsy data, together with a safety assessment from our ongoing studies.

Following our end of review meeting, we have held a productive dialogue with FDA regarding  the  REGENERATE
study to clarify data, a new consensus read methodology for liver biopsies, and analyses required to resubmit our NDA. We
are  also  in  the  process  of  generating  a  new  data  package  from  our  REGENERATE  study  using  the  new  liver  biopsy
consensus  read  methodology,  and  if  the  data  supports  accelerated  approval,  we  plan  to  have  a  potential  pre-NDA
submission meeting with the FDA during the first half of 2022. In December 2021, the Company withdrew its MAA as the
established application timeline could not be extended any further to allow for submission of additional safety and efficacy
data  being  generated  from  the  REGENERATE  study  and  the  Committee  for  Medicinal  Products  for  Human  Use  (the
“CHMP”) was not able to determine a positive benefit-risk based on previously submitted data. Once the additional data
from REGENERATE becomes available, the Company will assess the possibility of submitting a new application to the
EMA.

As part of our product development activities, we expect to continue to invest in evaluating the potential of OCA in
progressive  non-viral  liver  diseases.  We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with
compensated cirrhosis, known as the REVERSE trial. In January 2020, we announced that we completed enrollment of the
REVERSE trial with over 900 patients randomized. The liver biopsy samples from REVERSE are being evaluated utilizing
a similar, new consensus methodology to what we are using for REGENERATE. We expect top line data from our Phase 3
REVERSE trial in the third quarter of 2022.

We are evaluating the efficacy, safety and tolerability of OCA in combination with bezafibrate in patients with PBC in
a Phase 2 study outside of the United States. In the United States, we have an ongoing Phase 1 study to better characterize
the exposure response of the fixed-dose combination, and we have an open Investigational New Drug (“IND”) application
with the FDA. We are also in the process of initiating a second Phase 2 study in the United States. Our longer-term goal is
developing and seeking regulatory approval for a fixed dose combination regimen in PBC and potentially in other diseases.
In addition, we have other compounds in early stages of research and development in our pipeline, including our INT-787
compound, an FXR agonist. We are currently evaluating INT-787 in a Phase 1 clinical trial and plan to submit an IND in
the first half of 2022.

History and Development of the Company

For  a  full  discussion  of  the  general  development  of  the  Company’s  business,  see  the  Company’s  Annual  Report  on
https://www.sec.gov/Archives/edgar/data/
31, 

Form 
1270073/000155837021001804/icpt-20201231x10k.htm, which is incorporated by reference.

ended  December 

10-K 

2020 

year 

the 

for 

at 

Key developments that have occurred since January 1, 2021 include the following:

In  May  2021,  the  newly  identified  safety  signal,  or  NISS,  process  was  concluded  and  we  aligned  with  the  FDA  on
updated Ocaliva prescribing information in the United States, and Ocaliva is now contraindicated for patients with PBC
and  decompensated  cirrhosis,  a  prior  decompensation  event,  or  compensated  cirrhosis  with  evidence  of  portal
hypertension, in addition to the existing contraindication for complete biliary obstruction.

In August 2021, we agreed with a limited number of institutional holders of our 2023 Convertible Notes and our 2026
Convertible  Notes  maturing  May  15,  2026,  to  exchange  existing  notes  of  both  series  at  a  discount  for  new  2026
Convertible Secured Notes maturing February 15, 2026, and secured by a first priority security interest in substantially all
assets  of  Intercept  Pharmaceuticals,  Inc.  and  of  any  subsidiaries  that  meet  certain  threshold  requirements  to  become
guarantors. The noteholders (1) exchanged $306.5 million of 2023 Convertible Notes for $292.4 million of new notes, (2)
exchanged $114.7 million of 2026 Convertible Notes for $90.0 million of new notes, and also (3) subscribed to buy $117.6
million of new notes for cash. We thereby issued $500.0 million of 2026 Convertible Secured Notes at an interest rate of
3.50%.

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We received cash proceeds of $117.6 million. We also paid our financial advisory fee by issuing 769,823 new shares of
common  stock.  Further,  in  connection  with  the  exchange  and  sale,  we  bought  back  approximately  4.5  million  shares  of
common stock for $75.8 million in cash. In September 2021, we agreed with certain institutional holders to buy back $39.9
million of our 2023 Convertible Notes at a discount.

In December 2021, the Company withdrew its MAA with the EMA for conditional approval of OCA for liver fibrosis
due  to  NASH  as  the  established  application  timeline  could  not  be  extended  any  further  to  allow  for  submission  of
additional  safety  and  efficacy  data  being  generated  from  the  REGENERATE  study  and  the  CHMP  was  not  able  to
determine  a  positive  benefit-risk  based  on  previously  submitted  data.  Once  the  additional  data  from  REGENERATE
becomes available, the Company will assess the possibility of submitting a new application to the EMA.

In February 2022, the French subsidiary of the Company, Intercept Pharma France SAS (“ICPT France”), withdrew its
application  for  reimbursement  in  France  of  Ocaliva  for  treatment  of  PBC,  on  account  of  inability  to  reach  mutually
acceptable pricing terms with the Economic Committee for Health Products (“CEPS”), the French regulator for pricing and
reimbursement of pharmaceuticals. ICPT France initiated sales of Ocaliva in France prior to finalization of reimbursement
terms pursuant to a temporary use authorization (“ATU”).

In  February  2022,  the  Company  filed  a  terminal  disclaimer  in  the  United  States  Patent  and  Trademark  Office
concerning its RE 48,286 patent (“the '286 patent”), which is listed in the FDA Orange Book for OCALIVA. As a result of
the filing, the expiration date of the '286 patent changed from November 16, 2027 to February 21, 2027.

In February 2022, the Company entered into an Agreement of Lease with United States Fire Insurance Company as
landlord and the Company as tenant for space at 305 Madison Avenue, Morristown, NJ 07960. The Company intends to
move its principal executive offices and global headquarters there in connection with the expiration on March 31, 2022 of
its lease at 10 Hudson Yards, New York, NY 10001.

Our Strategy

Our  objective  is  to  develop  and  commercialize  novel  therapeutics  for  the  treatment  of  progressive  non-viral  liver

diseases with high unmet medical need. The key elements of our strategy are to:

● Further  strengthen  our  foundational  PBC  business.  We  intend  to  further  strengthen  our  foundational  PBC
business through expanding the market for Ocaliva for eligible patients by increasing Ocaliva’s penetration in
the markets where it has been approved, continuing to seek reimbursement in a number of countries where
we have been approved, and pursuing regulatory approval for Ocaliva in additional markets. In addition, we
continue  to  work  to  execute  on  our  post-marketing  regulatory  commitments  and  generate  new  data  with
respect to Ocaliva in the U.S. and Europe.

● Execute  on  our  clinical  and  regulatory  goals  and  timelines.  We  remain  focused  on  progressing  our
development program in liver fibrosis due to NASH and if the data supports accelerated approval, we plan to
have a potential pre-NDA submission meeting with the FDA during the first half of 2022. We also expect to
continue  our  Phase  3  REGENERATE  study  through  clinical  outcomes  and  to  progress  our  Phase  3
REVERSE  trial  for  NASH  patients  with  compensated  cirrhosis.  We  also  plan  to  advance  our  studies
evaluating bezafibrate in combination with OCA for PBC.

● Expand our portfolio and pipeline. We intend to identify additional opportunities to acquire, partner on, or in-
license new products and to develop OCA and our other product candidates, alone or in combination, in rare
liver  diseases.  In  addition,  we  intend  to  continue  to  advance  the  development  of  our  INT-787  compound,
which is an FXR agonist. We are currently evaluating INT-787 in a Phase 1 clinical trial and intend to submit
an IND in the first half of 2022.

● Improve  our  operational  and  financial  foundation.  We  intend  to  maintain  a  strong  and  experienced
leadership team to help to continue to drive Intercept’s growth and development while prudently managing
our expenses and cash position.

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● Expand and protect our intellectual property. We intend to continue to expand and aggressively prosecute our
intellectual property in the area of bile acid chemistry and therapeutics with the objective of maintaining a
valuable intellectual property portfolio and to vigorously defend and enforce our intellectual property rights
protecting Ocaliva.

Liver Function, Bile Acids and Progressive Non-Viral Liver Diseases

The  liver  performs  many  functions  that  are  vital  for  maintaining  health,  including  the  regulation  of  bile  acid
metabolism. Bile acids are natural detergent-like emulsifying agents that are released from the gallbladder into the intestine
when food is ingested, and are essential for the absorption of dietary cholesterol and other nutrients. Cholesterol bound by
bile acids is taken up by the liver, where the cholesterol is then converted into one of two primary bile acids. The bile acids
are  then  actively  secreted  into  bile  ducts,  which  eventually  empty  into  the  gallbladder.  This  digestive  cycle  of  bile  flow
from gallbladder to intestine to liver and back is called the enterohepatic recirculation of bile.

In  addition  to  facilitating  nutrient  absorption,  bile  acids  act  as  important  signals  that  help  regulate  multiple  other
biological functions. They are also complex signaling molecules that integrate metabolic and immune pathways involved in
the  healthy  functioning  of  various  tissues  and  organs.  For  example,  the  actions  of  bile  acids  in  the  liver,  intestine  and
kidney regulate repair mechanisms that modulate inflammation and fibrosis (scarring), which can lead to progressive organ
damage.

The biological effects of bile acids are mediated through dedicated receptors. The best understood receptor is FXR, a
nuclear receptor that regulates bile acid synthesis and clearance from the liver, thereby preventing excessive bile acid build-
up in the liver, which may be toxic. As such, FXR is a target for the treatment of several liver diseases such as PBC that
involve  impaired  bile  flow,  a  condition  called  cholestasis.  In  cholestasis,  the  liver  is  typically  exposed  to  higher  than
normal  levels  of  bile  acids,  which  can  cause  significant  damage  over  time.  In  addition,  bile  acid  activation  of  FXR  is
believed to induce anti-fibrotic, anti-inflammatory, anti-steatotic and other mechanisms that are necessary for the normal
regeneration of the liver. As a result, FXR is also a target for the treatment of more common liver diseases such as NASH
and alcoholic hepatitis. Further, based on the discovery of similar FXR-mediated protective mechanisms in other organs
exposed to bile acids, we believe that FXR may also be a potential target for the treatment of a number of intestinal, kidney
and other diseases.

OCA is a bile acid analog, a chemical substance that has a structure based on a naturally occurring human bile acid,
that selectively binds to and activates FXR. We believe that OCA has broad liver-protective properties and may effectively
counter a variety of chronic insults to the liver that cause fibrosis (scarring), which can eventually lead to cirrhosis, liver
transplant and death. Due to OCA’s bile acid-like properties, it circulates enterohepatically and engages FXR in both the
liver  and  intestine.  FXR  engagement  in  the  liver  is  believed  to  be  critical  to  successfully  treat  pathologic  injury  due  to
progressive underlying disease.

By  virtue  of  our  patent  portfolio  and  the  proprietary  know-how  of  our  employees  and  collaboration  partners,  we
believe that we hold a leading position in the fields of bile acid chemistry and therapeutics. Our research and development
efforts  have  resulted  in  a  pipeline  of  bile  acid  analogs  in  addition  to  OCA  and  through  our  on-going  work  with  our
collaboration partners such as Professor Roberto Pellicciari, Ph.D., one of our co-founders, and TES Pharma S.r.l., we are
continuing  our  research  to  rationally  design  compounds  that  bind  selectively  and  potently  to  FXR  and  other  bile  acid
receptors.

Our First Approved Product  

Ocaliva

Ocaliva  was  approved  for  PBC  by  the  FDA  in  May  2016  under  the  accelerated  approval  pathway.  We  commenced
sales and marketing of Ocaliva in the United States shortly after receiving approval, and Ocaliva is now available to U.S.
patients  primarily  through  a  network  of  specialty  pharmacy  distributors.  Ocaliva  received  conditional  approval  for  PBC
from  the  European  Commission  in  December  2016  and  we  commenced  our  European  (including  United  Kingdom)
commercial launch in January 2017. We have submitted dossiers and obtained, or are otherwise pursuing, reimbursement

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from  a  number  of  national  authorities  in  Europe.  Since  January  2017,  Ocaliva  has  also  received  regulatory  approval  in
several  of  our  target  markets  outside  the  United  States  and  Europe,  including  (but  not  limited  to)  Canada,  Israel  and
Australia, and we are pursuing marketing approval of Ocaliva for PBC in our other international target markets. Ocaliva
received orphan drug designation in both the United States and the European Union for the treatment of PBC.

Overview of PBC

PBC is a rare liver disease that primarily results from autoimmune destruction of the bile ducts that transport bile acids
out of the liver, resulting in cholestasis. The build-up of bile acids in the liver damages liver cells. These damaged liver
cells, in turn, release abnormal amounts of serum alkaline phosphatase (“ALP”), a liver enzyme that is a key biomarker of
the disease pathology. As shown in numerous clinical trials of treatment with UDCA (available generically as ursodiol), a
positive  therapeutic  response  is  primarily  determined  by  sustained  reduction  of  ALP  levels,  along  with  maintenance  of
normal bilirubin levels, indicating adequately compensated liver function. This biochemical improvement has been shown
to  correlate  well  with  improved  clinical  outcomes  such  as  transplant-free  survival.  As  the  disease  progresses,  it  causes
progressive  liver  damage  marked  by  chronic  inflammation  and  fibrosis.  Despite  its  rarity,  PBC  is  the  most  common
cholestatic  liver  disease  and  is  among  the  leading  indications  for  liver  transplant  among  women  in  the  United  States.
Disease  progression  in  PBC  varies  significantly,  with  median  survival  in  untreated  patients  estimated  to  be  7.5  years  if
symptomatic at diagnosis and up to 16 years if asymptomatic at diagnosis. PBC patients whose disease is progressing have
persistently  elevated  levels  of  ALP  and  other  liver  enzymes,  with  abnormal  bilirubin  levels  heralding  more  advanced
disease.  Data  from  published  long-term  studies  demonstrate  that  a  significant  portion  of  such  patients  with  advancing
disease progress to liver failure, transplant or death within five to ten years.

Based on our analysis of 2016 industry data, there were approximately 290,000 people with PBC at the time of our
U.S. launch in the United States, certain European countries, Canada, Australia and New Zealand. An estimated 90% of
PBC patients are women, with approximately one in 1,000 women over the age of 40 afflicted by the disease. The mean
age of diagnosis is about 40 years old and the typical initial presentation occurs between the ages of 30 and 65 years old. A
majority of PBC patients are asymptomatic at the time of initial diagnosis, but most develop symptoms over time. Fatigue
and pruritus are the most common symptoms in PBC patients. Less common symptoms include dry eyes and mouth, as
well as jaundice, which can be seen in more advanced disease. Based on the guidelines of the American Association for the
Study  of  Liver  Disease  and  the  European  Association  for  the  Study  of  the  Liver,  the  clinical  diagnosis  of  PBC  is
established  based  on  the  presence  of  (i)  a  positive  antimitochondrial  antibody  (“AMA”),  a  marker  of  this  autoimmune
disease seen in up to 95% of PBC patients and (ii) elevated serum levels of ALP. In the earlier stages of PBC, ALP is often
the  only  abnormally  elevated  liver  enzyme,  rising  to  between  two  to  ten  times  higher  than  normal  values.  Bilirubin  is  a
marker of liver function and is also monitored in PBC to provide an indication of how well the liver is functioning. Liver
biopsy can be used to confirm the diagnosis of PBC, but is not required and is becoming less-frequently performed.

A  number  of  published  clinical  studies  have  demonstrated  that  lower  levels  of  ALP,  both  independently  or  in
conjunction with normal bilirubin levels, correlate with a significant reduction in adverse clinical outcomes such as liver
transplant and/or death in PBC patients. These studies include the result of meta-analyses of PBC clinical outcomes data of
more than 6,000 PBC patients from 17 academic centers in eight countries that have been compiled by the Global PBC
Study Group, which we sponsored, as well as a dataset of over 6,000 PBC patients across the United Kingdom compiled by
the UK PBC Group.

Prior to Ocaliva, the only approved drug indicated for the treatment of PBC was UDCA, which is widely considered
the  standard  first-line  therapy  for  PBC  patients.  In  patients  for  whom  UDCA  is  effective,  the  treatment  slows  the
progression of PBC, reducing the likelihood of liver failure and the need for transplant.

Phase 3 POISE Trial

Ocaliva’s accelerated approval in the United States and conditional approval in the European Union was supported by
the results of our Phase 3 POISE trial, which was completed in March 2014. The data from the POISE trial showed that
Ocaliva, at both a once-daily 10 mg dose and a once-daily 5 mg dose titrated to 10 mg, met the trial’s primary endpoint of
achieving a reduction in ALP to below a threshold of 1.67 times the upper limit of normal (“ULN”), with a minimum of a

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15%  reduction  in  ALP  level  from  baseline,  and  a  normal  bilirubin  level  after  12  months  of  therapy.  The  percentage  of
patients meeting the POISE trial’s primary endpoint was 10% in the placebo group, 47% in the 10 mg Ocaliva group and
46% in the Ocaliva titration group (both dose groups p < 0.0001 as compared to placebo) in an intent-to-treat analysis. The
placebo group experienced a mean decrease in ALP from baseline of 5%, compared to a mean decrease of 39% in the 10
mg  Ocaliva  dose  group  and  33%  in  the  Ocaliva  titration  group  (both  dose  groups  p  <  0.0001  as  compared  to  placebo).
Pruritus, generally mild to moderate, was the most frequently reported adverse event associated with Ocaliva treatment and
was  observed  in  38%  of  patients  on  placebo,  70%  of  patients  in  the  10  mg  Ocaliva  group  and  56%  of  patients  in  the
Ocaliva titration group. Eight patients discontinued due to pruritus, of whom none were in the placebo group, seven (10%)
were in the 10 mg Ocaliva group and one (1%) was in the Ocaliva titration group. Decreases in high density lipoprotein
(“HDL”) cholesterol were also observed during treatment.

Following  the  completion  of  the  double-blind  portion  of  the  POISE  trial  described  above,  patients  were  given  the
option to enroll in a five-year open-label long-term safety and efficacy extension trial, which has been completed. Patients
received Ocaliva at a once-daily 5 mg dose for three months, after which patients were titrated based on tolerability. The
data from the open-label extension portion of the trial showed that 46% of patients responded after 12 months of treatment
with Ocaliva and 50% to 56% of patients responded after 48 to 72 months of treatment with Ocaliva (based on the same
criteria used to define the primary endpoint in the 12 month placebo controlled trial). Reductions in ALP were sustained
through the double-blind and extension portions of the trial and total bilirubin levels remained stable and within the normal
range for most patients for the duration of the trial (ALP p < 0.0001 for all post-baseline visits; total bilirubin: p-values
were not consistently significant throughout the extension portion of the POISE trial). Adverse events were consistent with
the safety profile of Ocaliva in patients with PBC. The most commonly reported adverse events were pruritis and fatigue,
which were generally mild to moderate in severity.

In  November  2021,  we  presented  the  results  of  an  analysis  of  clinical  outcomes  in  patients  with  PBC  treated  with
Ocaliva in the POISE Phase 3 study and its open label extension compared to propensity score matched external controls
from the UK and Global PBC cohorts, as a late-breaking podium presentation at The Liver Meeting, the Annual Meeting of
the  American  Association  for  the  Study  of  Liver  Diseases  (AASLD).  The  study  results  showed  statistically  significant
greater transplant-free survival in patients receiving obeticholic acid as compared to the control groups.

Ongoing Confirmatory Clinical Outcomes Trial and Other Post Marketing Requirements

In  connection  with  Ocaliva’s  accelerated  approval  in  the  United  States  and  conditional  approval  in  the  European
Union, we committed to conduct a Phase 4 confirmatory outcomes trial of Ocaliva, known as the COBALT trial, and other
clinical  trials  to  satisfy  post-marketing  regulatory  requirements.  Continued  approval  of  Ocaliva  for  PBC  in  the  United
States, the European Union and other jurisdictions is contingent upon the verification and description of clinical benefit in
the COBALT trial and our satisfaction of our other post-marketing regulatory requirements. Any delay or failure by us to
satisfy  such  requirements,  including  any  delay  or  failure  relating  to  our  Phase  4  COBALT  trial,  may  jeopardize  the
continued approval of Ocaliva for PBC in the United States, European Union and other jurisdictions.

The goal of the COBALT trial is to confirm that reduction of ALP based upon Ocaliva treatment is associated with a
longer-term benefit on liver-related clinical outcomes. COBALT was designed to assess the effect of a once-daily dose of 5
mg or 10 mg of Ocaliva in approximately 430 PBC patients with an inadequate therapeutic response to UDCA or who were
unable  to  tolerate  UDCA.  Under  COBALT’s  previous  study  design,  eligible  patients  with  PBC  continued  their  UDCA
treatment,  except  for  those  patients  unable  to  tolerate  UDCA,  and  were  randomized  into  one  of  two  treatment  arms  of
approximately  215  patients  each,  receiving  either  (i)  a  placebo  or  (ii)  Ocaliva  starting  at  5  mg  and  increasing  over  the
course  of  the  trial  to  10  mg  of  Ocaliva  based  on  tolerability.  Dosing  frequency  was  determined  by  disease  stage.  The
primary  endpoint  of  the  trial  was  based  on  clinical  outcomes  as  measured  by  time  to  first  occurrence  of  any  of  the
following  adjudicated  events:  death  (all-cause),  liver  transplant,  Model  of  End  Stage  Liver  Disease  (“MELD”)  score
greater  than  15,  uncontrolled  ascites  or  hospitalization  due  to  variceal  bleeding,  hepatic  encephalopathy  or  spontaneous
bacterial peritonitis. The study was designed to evaluate subjects across the spectrum of PBC disease, including early and
advanced PBC. As part of the closure of COBALT, we have discussed endpoint changes with the FDA.

Further,  as  part  of  our  post-marketing  requirements  for  Ocaliva,  we  undertook  a  Phase  4  clinical  trial  of  Ocaliva  in

patients with PBC who have moderate to severe hepatic impairment (Child-Pugh B and C) (known as the 401 trial). This

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double-blind,  placebo-controlled  study  was  designed  to  evaluate  the  pharmacokinetics  of  Ocaliva  and  its  conjugates,  as
well as safety and tolerability. Additional objectives included an evaluation of Ocaliva treatment compared to placebo on
liver biochemistry, Child-Pugh scores and non-invasive markers of liver fibrosis and stiffness. The trial as designed was
targeted  to  enroll  approximately  50  patients  in  the  United  States,  Europe  and  other  jurisdictions  for  48  weeks,  but
ultimately enrolled a lower number of patients and was closed.

Changes to our Ocaliva label with respect to patients with PBC with decompensated cirrhosis (e.g., Child-Pugh Class
B  or  C),  a  prior  decompensation  event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension  influenced
modifications  to  our  COBALT  study  design  and  as  a  result  of  the  changes  to  the  U.S.  prescribing  information  we  also
removed from the trial subjects in the United States who are now excluded from the scope of the label. We also agreed with
the  FDA  and  the  EMA  to  terminate  our  401  trial,  in  light  of  the  exclusion  of  patients  with  PBC  with  decompensated
cirrhosis  from  the  Ocaliva  label  in  the  U.S.  In  addition,  while  we  remain  blinded  to  safety  and  efficacy  data  in  the
COBALT  trial  and  401  trial,  a  data  monitoring  committee  (“DMC”)  reviewed  the  unblinded  results  of  a  pre-specified
interim  efficacy  analysis  of  the  COBALT  trial  and  separately  reviewed  unblinded  safety  and  pharmacokinetic  data  from
both  the  COBALT  and  401  trials.  Following  these  reviews,  the  DMC  stated  that  it  was  not  feasible  to  continue  the
COBALT trial as designed and noted the challenges in enrolling and maintaining placebo-controlled post-marketing studies
in this rare disease setting. No acute safety concerns were noted by the DMC. Given the feasibility concerns noted by the
DMC  as  well  as  the  potential  confounding  impact  of  subjects  discontinuing  treatment  and/or  transitioning  from
investigational  product  to  commercial  drug  during  clinical  trials,  we  discussed  with  the  FDA  and  the  EMA  proposed
modifications  to  the  COBALT  trial,  and  we  notified  the  FDA  and  the  EMA  of  the  DMC’s  recommendation.  Based  on
discussions with both the FDA and EMA, which are ongoing, we are in the process of closing out the COBALT trial. We
will continue to generate placebo controlled data from the COBALT trial as well as data from studies utilizing real world
evidence in support of a broader evidence data package, which we anticipate submitting to the FDA and the EMA in the
second half of 2022. If this data package does not support fulfillment of our post-marketing obligations, we may not be
able to maintain our previously granted marketing approvals of Ocaliva for PBC.

We are also undertaking a Phase 2 clinical trial of Ocaliva in pediatric patients with biliary atresia, a life-threatening
condition in infants in which the bile ducts inside or outside the liver do not have normal openings. This trial, known as the
CARE  trial,  is  a  part  of  an  EMA-approved  Pediatric  Investigation  Plan  (“PIP”)  supporting  the  conditional  approval  of
Ocaliva for PBC in the European Union as PBC is extremely rare in the pediatric population. The CARE trial is designed
to  evaluate  the  effects  of  Ocaliva  treatment  where  patients  with  biliary  atresia  are  randomized  to  varying  doses.  The
primary  endpoint  is  to  evaluate  the  pharmacokinetics  and  the  safety  and  tolerability  of  Ocaliva  treatment.  In  addition,
Ocaliva’s effect on hepatobiliary indices and biomarkers will be assessed.

Ocaliva Label Update

In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended  weekly  dose  in  such  patients.  As  a  result,  in  September  2017,  we  issued  a  Dear  Health  Care  Provider
(“DHCP”)  letter,  and  the  FDA  also  subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended
label dosing. Both communications remind healthcare providers of the importance of the recommended reduced dosing of
Ocaliva in PBC patients with moderate or severe hepatic impairment, while reiterating the importance of monitoring PBC
patients  for  progression  of  their  disease  and  the  occurrence  of  liver-related  adverse  reactions.  In  addition  to  the  DHCP
letter,  we  took  actions  to  enhance  education  about  appropriate  use  of  Ocaliva.  These  initiatives  included:  reeducating
physicians  on  the  label,  with  a  focus  on  ensuring  appropriate  dosing  for  patients  with  moderate  or  severe  hepatic
impairment; enhancing monitoring of patients for liver-related adverse reactions; and adjudicating reported cases of serious
liver injury, including in patients with no or mild hepatic impairment.

In February 2018, we announced that the Ocaliva label in the United States had been updated by the FDA to include a
boxed warning and a dosing table that reinforced the then-existing dosing schedule for patients with Child-Pugh Class B or
C  or  decompensated  cirrhosis.  In  addition,  the  FDA  issued  an  updated  drug  safety  communication  to  accompany  the
revised label. We remain focused on the safety of all of the patients using Ocaliva within and outside of our ongoing

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clinical studies and have engaged with relevant regulatory authorities to ensure that the Ocaliva label sufficiently reinforces
the importance of appropriate dosing in patients with advanced cirrhosis.

The FDA notified us that, in the course of its routine safety surveillance, in May 2020 the FDA began to evaluate a
newly identified safety signal, or NISS, regarding liver disorder for Ocaliva which the FDA classified as a potential risk.
The FDA informed us that its review of the NISS was focused on a subset of the cirrhotic, or more advanced, PBC patients
who  had  taken  Ocaliva.  As  part  of  our  routine  pharmacovigilance  efforts,  we  worked  with  the  FDA  to  reconcile  our
internal  safety  database  with  the  FDA  Adverse  Event  Reporting  System  database  and  we  completed  a  comprehensive
assessment of all available data, including data from our completed clinical trials, blinded reviews of ongoing clinical trial
data,  unblinded  reviews  of  certain  ongoing  clinical  trial  data  by  the  DMC,  post-marketing  data  and  natural  history  data,
which we submitted to the FDA and had a meeting in 2021 to discuss.

In  May  2021,  the  NISS  process  was  concluded  and  we  aligned  with  the  FDA  on  updated  Ocaliva  prescribing
information in the United States, and Ocaliva is now contraindicated for patients with PBC and decompensated cirrhosis, a
prior  decompensation  event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension,  in  addition  to  the  existing
contraindication  for  complete  biliary  obstruction.  We  are  also  working  with  the  CHMP  to  update  our  European  Ocaliva
label, which we expect will occur in 2022.

Our Product Candidates

The following summarizes the current status and the anticipated next steps in our development plans for our product
candidates.  We  continually  evaluate  each  product  candidate  in  an  effort  to  efficiently  allocate  research  and  development
funds to projects we deem to be in our best interests based on, among other factors, the product candidate’s performance in
pre-clinical  and/or  clinical  studies,  our  expectations  regarding  the  potential  future  regulatory  approval  of  the  product
candidate and our view of the potential commercial viability of the product candidate in light of market conditions.

OCA for liver fibrosis due to NASH

Our lead product candidate is OCA for the potential treatment of liver fibrosis due to NASH. In February 2019, we
announced  topline  results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in
patients with liver fibrosis due to NASH, known as the REGENERATE trial. In the primary efficacy analysis, once-daily
OCA  25  mg  met  the  primary  endpoint  agreed  with  the  FDA  of  fibrosis  improvement  by  at  least  one  stage  with  no
worsening of NASH at the planned 18-month interim analysis. Adverse events were generally mild to moderate in severity
and  the  most  common  were  consistent  with  the  known  profile  of  OCA.  OCA  has  received  breakthrough  therapy
designation from the FDA for the treatment of NASH patients with liver fibrosis. In September 2019, we submitted a NDA
seeking  accelerated  approval  of  OCA  for  liver  fibrosis  due  to  NASH  in  the  United  States  and,  in  December  2019,  we
submitted a MAA seeking conditional approval of OCA for liver fibrosis due to NASH in Europe. The FDA subsequently
accepted our NDA for filing and granted a priority review designation for OCA for liver fibrosis due to NASH. In January
2020, the EMA validated our MAA and thereby confirmed that our MAA was sufficiently complete to begin the formal
review  process.  In  June  2020,  we  received  a  complete  response  letter  (“CRL”)  from  the  FDA  stating  that  our  NDA  for
OCA for the treatment of liver fibrosis due to NASH could not be approved in its present form. The CRL indicated that,
based on the data the FDA had reviewed, the FDA has determined that the predicted benefit of OCA based on a surrogate
histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently  outweigh  the  potential  risks  to  support  accelerated
approval for the treatment of patients with liver fibrosis due to NASH. At that time, the FDA recommended that we submit
additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing  REGENERATE  trial  in  support  of  potential
accelerated approval and that the long-term outcomes phase of the trial should continue. In October 2020, we had our end
of  review  meeting  with  the  FDA  to  discuss  the  FDA’s  risk-benefit  assessment  in  the  CRL  based  on  its  review  of  the
available  data,  as  well  as  our  proposed  resubmission  of  our  NDA  for  the  treatment  of  liver  fibrosis  due  to  NASH.  The
meeting was constructive and the FDA has provided us with helpful guidance regarding supplemental data we can provide
to  further  characterize  OCA’s  efficacy  and  safety  profile  that  could  support  resubmission  based  on  our  Phase  3
REGENERATE 18-month biopsy data, together with a safety update from our ongoing studies.

Following our end of review meeting, we have held a productive dialogue with FDA regarding the REGENERATE

study to clarify data, a new consensus read methodology for liver biopsies, and analyses required to resubmit our NDA.

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We are also in the process of generating a new data package from our REGENERATE study using the new liver biopsy
consensus  read  methodology,  and  if  the  data  supports  accelerated  approval,  we  plan  to  have  a  potential  pre-NDA
submission  meeting  with  the  FDA  during  the  first  half  of  2022.  With  respect  to  our  European  submission  seeking
conditional approval of OCA for liver fibrosis due to NASH, in December 2021 we withdrew our MAA as the established
application timeline could not be extended any further to allow for submission of additional safety and efficacy data being
generated  from  the  REGENERATE  study  and  the  CHMP  was  not  able  to  determine  a  positive  benefit-risk  based  on
previously submitted data. Once the additional data from REGENERATE becomes available, the Company will assess the
possibility of submitting a new application to the EMA.

In  addition,  we  have  conducted  a  number  of  other  trials  and  studies  in  connection  with  our  NASH  development
program, and our Phase 3 trial in NASH patients with compensated cirrhosis, known as the REVERSE trial, is ongoing. We
expect top line data from our Phase 3 REVERSE trial in the third quarter of 2022.

Overview of NASH

NASH is a serious progressive liver disease caused by excessive fat accumulation in the liver (steatosis) that induces
chronic  inflammation,  resulting  in  progressive  fibrosis  (scarring)  that  can  lead  to  cirrhosis,  eventual  liver  failure,  cancer
and death. More than 20% of patients with NASH are estimated to progress to cirrhosis within a decade of diagnosis and,
compared  to  the  general  population,  have  a  ten-fold  greater  risk  of  liver-related  mortality.  The  proportion  of  liver
transplants attributable to NASH has increased rapidly in recent years with NASH currently the second leading cause of
liver transplantation in the United States and, in females, the leading cause. NASH is anticipated to become the leading
indication  for  liver  transplantation  in  Europe  within  the  next  decade.  Additionally,  NASH  is  a  leading,  and  a  rapidly
increasing,  cause  of  hepatocellular  carcinoma  (primary  liver  cancer),  of  which  up  to  40%  of  cases  in  NASH  patients
develop prior to developing cirrhosis.

Although  difficult  to  precisely  estimate,  epidemiology  research  estimates  that  the  global  prevalence  of  NASH  is
approximately  3  –  5%  and  is  expected  to  increase  markedly  by  2030.  Fibrosis  is  the  most  robust  predictor  of  long-term
overall mortality, liver transplantation and liver-related events in patients with NASH and advanced fibrosis is associated
with a substantially higher risk of liver-related morbidity and mortality in patients with NASH. We believe that a majority
of  NASH  patients  diagnosed  and  under  specialist  care  have  fibrosis  of  stage  2  or  greater.  Although  the  prevalence  of
NASH  is  lower  in  children,  it  has  also  become  a  serious  disease  burden  in  the  pediatric  population.  Other  common  co-
existing conditions such as obesity and type 2 diabetes, which are present in a majority of NASH patients, raise important
risks. NASH has been linked in both developed and developing countries to the adoption of a Western diet, with increased
consumption of processed foods containing polyunsaturated fatty acids and fructose.

Generally  in  clinical  trials  in  NASH,  a  definitive  diagnosis  requires  a  histologic  assessment  of  a  liver  biopsy  for
several key features associated with NASH, including, but not limited to, steatosis, lobular inflammation and hepatocyte
ballooning. However, we believe that the majority of NASH patients currently under treater care have been assessed for
liver  fibrosis  without  a  liver  biopsy.  Several  imaging  and  circulating  biomarkers  are  being  investigated  as  non-invasive
diagnostic methods, including transient elastography (an ultrasound technology approved in the United States and Europe
for the measurement of liver fibrosis), magnetic resonance imaging and serum biomarkers. NASH diagnosis rates in the
United States and the EU5 countries are very low, owing to a lack of approved treatment options and a lack of validated
non-invasive  diagnosis  options.  We  believe  the  availability  of  novel  therapeutics  and  non-invasive  technologies  will  be
instrumental in improving diagnosis rates.

There  are  currently  no  medications  approved  for  the  treatment  of  NASH  in  the  United  States  or  Europe.  However,
various  therapeutics  are  used  “off-label”,  such  as  vitamin  E  (an  antioxidant),  insulin  sensitizers  (e.g.,  metformin,
pioglitazone),  pentoxifylline  and  UDCA.  Lifestyle  changes,  including  modification  of  diet  and  exercise  to  reduce  body
weight, as well as treatment of concomitant diabetes and dyslipidemia, are commonly accepted as the standard of care, but
have  not  conclusively  been  shown  to  prevent  disease  progression.  Although  some  of  the  off-label  treatments  described
above have been studied as possible treatments for NASH, none has been approved by the FDA or EMA as a treatment for
this disease. Currently, treatment options for NASH patients with advanced cirrhosis are limited. Although liver transplant
can  be  life-saving,  many  patients  fail  to  receive  a  donor  organ  in  time,  and  for  those  who  do,  there  are  very  significant
clinical risks, such as infection and organ rejection, as well as significant costs. In addition, the post-transplant

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recurrence rate of NASH has been shown to be as high as 25% at 18 months. Given the lack of available treatment options,
we believe that there is a significant unmet need for novel therapies for NASH, particularly in those patients with advanced
fibrosis and cirrhosis and those with a high risk of disease progression due to other co-morbidities such as type 2 diabetes.

FXR  activation  has  been  shown  to  play  a  key  role  in  the  regulation  of  the  metabolic  pathways  relevant  to  NASH,
highlighting  FXR  as  a  potential  drug  target  for  treatment  of  the  disease.  Given  the  significant  unmet  medical  need  of
patients  with  NASH,  we  believe  that  the  ability  of  OCA  to  potently  activate  FXR  has  the  potential  to  convey  clinical
benefit by improving key histologic parameters of the disease. This is supported by our preclinical and clinical results to
date, and is being further investigated in our ongoing clinical trial program.

Phase 3 REGENERATE Trial

We are currently conducting a pivotal Phase 3 clinical trial of OCA in patients with liver fibrosis due to NASH, known
as the REGENERATE trial. REGENERATE is a randomized, double-blind, placebo-controlled, multicenter study assessing
the safety and efficacy of OCA on liver-related clinical outcomes in patients with liver fibrosis due to NASH. Patients with
biopsy proven NASH with fibrosis are randomized 1:1:1 to receive placebo, OCA 10 mg or OCA 25 mg once daily. In
August  2019,  we  announced  the  completion  of  the  enrollment  of  the  clinical  outcomes  cohort  of  REGENERATE,  with
2,480  adult  NASH  patients  with  fibrosis  randomized  at  over  300  qualified  centers  worldwide.  REGENERATE  will
continue  through  clinical  outcomes  for  verification  and  description  of  clinical  benefit.  The  end-of-study  analysis  will
evaluate the effect of OCA on all-cause mortality and liver-related clinical outcomes.

An  18-month  interim  analysis  was  conducted  to  assess  the  effect  of  OCA  in  liver  histology  comparing  month  18
biopsy  with  baseline.  Patients  without  a  repeat  biopsy  due  to  study  discontinuation  or  other  reason  were  treated  as  non-
responders  in  the  primary  efficacy  analysis  and  full  efficacy  analysis  (each  as  described  below).  A  smaller  exploratory
cohort of patients with stage 1 liver fibrosis and at least one accompanying comorbidity (specified as diabetes, obesity or
alanine transaminase (“ALT”) greater than 1.5 times ULN) were also enrolled in REGENERATE, but were not included in
the  primary  efficacy  analysis.  As  described  below,  these  patients  were  included  in  the  full  efficacy  analysis  and  safety
analysis.  The  end-of-study  analysis  will  evaluate  the  effect  of  OCA  on  all-cause  mortality  and  liver-related  clinical
outcomes.

In February 2019, we announced topline results from the REGENERATE trial interim analysis. In the primary efficacy
analysis, once-daily OCA 25 mg met, with statistical significance, the primary endpoint agreed with the FDA of fibrosis
improvement by at least one stage with no worsening of NASH (defined as no worsening of hepatocellular ballooning, no
worsening  of  lobular  inflammation  and  no  worsening  of  steatosis)  at  the  planned  18-month  analysis  and  adverse  events
were  generally  mild  to  moderate  in  severity  and  the  most  common  were  consistent  with  the  known  profile  of  OCA.
Although  a  numerically  greater  proportion  of  patients  in  both  OCA  treatment  arms  compared  to  placebo  achieved  the
primary endpoint of NASH resolution with no worsening of liver fibrosis in the primary efficacy analysis, this result did
not  reach  statistical  significance.  NASH  resolution  is  defined  as  the  overall  histopathologic  interpretation  of  (i)  no  fatty
liver disease or (ii) fatty liver disease (simple or isolated steatosis) without steatohepatitis AND a nonalcoholic fatty liver
disease (“NAFLD”) activity score (“NAS”) of 0 for ballooning and 0-1 for inflammation. As agreed with the FDA, in order
for  the  primary  objective  to  be  met,  the  study  was  required  to  achieve  one  of  the  two  primary  endpoints.  In  November
2019, the results of the 18-month interim analysis from the REGENERATE trial were published in The Lancet.

The “primary efficacy analysis” (Intent-to-Treat or “ITT”) assessed efficacy at 18 months in 931 patients with stage 2
or 3 liver fibrosis due to NASH. Overall study discontinuations in the primary efficacy analysis population were balanced
across  treatment  arms:  16%  in  placebo,  17%  in  OCA  10  mg  and  15%  in  OCA  25  mg.  An  additional  pre-specified  “full
efficacy  analysis”  at  18  months  added  an  exploratory  cohort  of  287  NASH  patients  with  stage  1  liver  fibrosis  and
additional risk factors who were at increased risk of progression to cirrhosis (N = 1,218).

Set forth below is a summary of the 18-month primary efficacy analysis and additional full efficacy analysis from the

REGENERATE trial.

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Fibrosis Improvement at Month 18

Primary Efficacy Analysis 
(ITT population: NASH with stage 2 and 3 liver fibrosis)

Placebo
n = 311

OCA 10 mg
n = 312

OCA 25 mg
n= 308

Fibrosis improvement (≥ 1 stage) with no worsening of NASH*

Additional Full Efficacy Analysis  
     (ITT population plus stage 1 liver fibrosis patients)
Fibrosis improvement (≥ 1 stage) with no worsening of NASH*

11.9%

Placebo 
n=407
10.6%

17.6%
p = 0.0446
OCA 10 mg
n = 407
15.7%
p = 0.0286

23.1%
p = 0.0002**
OCA 25 mg
n = 404
21%
p < 0.0001

*    Defined as no worsening of hepatocellular ballooning, no worsening of lobular inflammation and no worsening of 
steatosis.
** Statistically significant in accordance with the statistical analysis plan agreed with the FDA.

NASH Resolution at Month 18

Primary Efficacy Analysis
(ITT population: NASH with stage 2 and 3 liver fibrosis
NASH resolution‡ with no worsening of liver fibrosis stage

Additional Full Efficacy Analysis
    (ITT population plus stage 1 liver fibrosis patients)
NASH resolution‡ with no worsening of liver fibrosis stage

Placebo
n = 311
8.0%

Placebo
n = 407
7.9%

OCA 10 mg
n = 312
11.2%
p = 0.1814
OCA 10 mg
n = 407
11.3%
p = 0.0903

OCA 25 mg
n = 308
11.7%
p = 0.1268
OCA 25 mg
n = 404
14.9%
p = 0.0013

‡ Defined as the overall histopathologic interpretation of (i) no fatty liver disease or (ii) fatty liver disease (simple or
isolated steatosis) without steatohepatitis AND a NAS of 0 for ballooning and 0-1 for inflammation.

The “safety population” in the planned 18-month analysis of REGENERATE included 1,968 randomized patients who

received at least one dose of investigational product (OCA or placebo).

Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most  common  were  consistent  with  the  known
profile of OCA. The frequency of serious adverse events was similar across treatment arms (11% in placebo, 11% in OCA
10 mg and 14% in OCA 25 mg) and no serious adverse event occurred in > 1% of patients in any treatment arm. There
were  3  deaths  (2  in  placebo:  bone  cancer  and  cardiac  arrest,  1  in  OCA  25  mg:  glioblastoma)  and  none  were  considered
related to treatment.

The most common adverse event reported was dose-related pruritus (19% in placebo, 28% in OCA 10 mg and 51% in
OCA  25  mg).  The  large  majority  of  pruritus  events  were  mild  to  moderate,  with  severe  pruritus  occurring  in  a  small
number  of  patients  (<  1%  in  placebo,  <  1%  in  OCA  10  mg  and  5%  in  OCA  25  mg).  A  higher  incidence  of  pruritus
associated treatment discontinuation was observed for OCA 25 mg (< 1% in placebo, < 1% in OCA 10 mg and 9% in OCA
25 mg). According to the clinical study protocol, investigator assessed severe pruritus mandated treatment discontinuation.

Consistent  with  observations  from  previous  NASH  studies,  OCA  treatment  was  associated  with  an  increase  in  low
density lipoprotein (“LDL”) cholesterol, with a peak increase of 22.6 mg/dL at four weeks and subsequently reversing and
approaching  baseline  at  month  18  (4.0  mg/dL  increase  from  baseline).  Statin  therapy  was  initiated  in  10%  of  placebo
patients  and  24%  of  each  OCA  treatment  arm.  Among  OCA  patients  who  initiated  statins,  LDL  cholesterol  increases
reversed  and  fell  to  below  baseline  levels  by  month  6.  Triglycerides  rapidly  and  continually  decreased  in  the  OCA
treatment arms through month 18. There were few and varied serious cardiovascular events and incidence was balanced
across the three treatment arms (2% in placebo, 1% in OCA 10 mg and 2% in OCA 25 mg).

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In patients with type 2 diabetes, OCA treatment was associated with an early transient increase in fasting glucose and
hemoglobin A1c with return to levels similar to placebo by month 6. No clinically meaningful changes were noted in non-
diabetic patients.

With  respect  to  hepatobiliary  events,  more  patients  (3%)  on  OCA  25  mg  experienced  gallstones  or  cholecystitis
compared to < 1% on placebo and 1% on OCA 10 mg. While numerically higher in the OCA 25 mg treatment arm, serious
hepatic adverse events were uncommon with < 1% incidence in each of the three treatment arms.

Phase 3 REVERSE Trial

We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with  compensated  cirrhosis,  known  as  the
REVERSE trial. REVERSE is a randomized, double-blind, placebo-controlled, multicenter trial evaluating the safety and
efficacy  of  OCA  in  NASH  patients  with  compensated  cirrhosis.  In  January  2020,  we  announced  that  we  completed
enrollment  of  the  REVERSE  trial  with  over  900  patients  with  a  biopsy-confirmed  diagnosis  of  cirrhosis  due  to  NASH
randomized. We expect top line data from our Phase 3 REVERSE trial in the third quarter of 2022.

The primary endpoint for REVERSE is the percentage of subjects with histological improvement in fibrosis by at least
one  stage  with  no  worsening  of  NASH  using  the  NASH  Clinical  Research  Network  scoring  system  after  18  months  of
treatment. Patients are randomized 1:1:1 into one of three treatment arms receiving a once-daily dose of placebo, OCA 10
mg or OCA 10 mg for the first three months with titration in accordance with the study protocol up to OCA 25 mg for the
remaining study period. Patients who successfully complete the double-blind phase of REVERSE will be eligible to enroll
in an open-label extension phase for up to 12 additional months.

Phase 2 CONTROL Trial

In  December  2015,  we  initiated  a  Phase  2  clinical  trial,  known  as  the  CONTROL  trial,  to  characterize  the  lipid
metabolic  effects  of  OCA  and  cholesterol  management  effects  of  concomitant  statin  administration  in  NASH  patients.
CONTROL enrolled approximately 80 NASH patients who were naïve to statin therapy or had undergone a statin washout
period. Statin-naïve or washout patients were randomized to receive one of three doses of OCA (5 mg, 10 mg or 25 mg) or
placebo. The study included a 16-week double-blind phase followed by an optional long-term safety extension (“LTSE”).

In July 2017, we announced that CONTROL met its primary objective by showing that newly initiated treatment with
atorvastatin rapidly reversed OCA-associated increases in LDL cholesterol to below baseline levels. Most of the effect was
observed  four  weeks  after  initiation  of  the  lowest  available  dose  of  atorvastatin  and  was  sustained  throughout  the  study
period. OCA treatment in the absence of statin therapy over the first four weeks resulted in an increase in LDL cholesterol
across all OCA treatment groups, while the placebo group was relatively unchanged. Treatment with atorvastatin beginning
at week four and continuing through week 16 reversed OCA-related increases in LDL cholesterol to below baseline levels
in all OCA treatment groups. Dose-dependent pruritus was the most common adverse event in patients treated with OCA,
occurring in 5% of patients on placebo, 5% of patients in the OCA 5 mg group, 10% of patients in the OCA 10 mg group
and 55% of patients in the OCA 25 mg group. All adverse events were mild to moderate and two patients discontinued
treatment  in  the  OCA  25  mg  group  due  to  pruritus.  Over  95%  of  the  patients  completing  the  double-blind  phase  of
CONTROL enrolled in the LTSE phase of the trial. During the LTSE phase of CONTROL, there was one patient death,
which the principal investigator determined was unlikely related to OCA.

Phase 2 Sumitomo Dainippon Trial

In October 2015, we announced the results of a 72-week Phase 2 dose ranging trial of OCA in 200 adult patients with
NASH in Japan. The trial was conducted by our former collaborator, Sumitomo Dainippon Pharma Co., Ltd. (“Sumitomo
Dainippon”). In this trial, 202 Japanese biopsy-proven NASH patients (NAS of 5-8) were randomized into one of four arms
to  receive  either  a  10  mg,  20  mg  or  40  mg  dose  of  OCA  or  placebo,  and  200  of  these  patients  (50  per  group)  initiated
treatment for a 72-week double-blind treatment phase, followed by a 24-week off treatment phase. The primary endpoint
was histologic improvement defined as at least a two-point improvement in NAS with no worsening of fibrosis.

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The primary efficacy analysis was conducted on an ITT basis, testing the dose dependent effects of once daily OCA
(10 mg, 20 mg and 40 mg) versus placebo on the primary endpoint. The ITT analysis included all randomized patients who
received  treatment  (50  per  group),  and  patients  who  discontinued  or  did  not  have  a  repeat  biopsy  were  treated  as  non-
responders.  A  pre-specified  completer  analysis  was  conducted  on  the  patients  who  had  biopsies  at  both  baseline  and  72
weeks (45, 44, 44 and 37 patients in the placebo, OCA 10 mg, OCA 20 mg and OCA 40 mg groups, respectively).

The  Sumitomo  Dainippon  trial  did  not  meet  statistical  significance  for  the  primary  endpoint.  The  ITT  results  in  the
table below show a dose dependent increase in the percentage of OCA-treated patients compared to placebo who achieved
the  primary  endpoint  (p  =  0.053).  Dose-dependent  trends  not  reaching  statistical  significance  were  observed  for  several
other pre-specified histologic endpoints, including the percentage of patients with steatosis and inflammation improvement,
ballooning resolution and NASH resolution. No difference was seen in fibrosis improvement in the OCA groups compared
to placebo.

ITT Results
NAS improvement > 2 points with
   no worsening of fibrosis

Placebo
N = 50
10 (20%)  

OCA 10 mg
N = 50
11 (22%)
p = 0.8070** 

OCA 20 mg
N = 50
14 (28%)
p = 0.3378** 

OCA 40 mg
N = 50
19 (38%)
p = 0.0496** 

p = 0.053*

*            Primary  efficacy  analysis  is  a  stratified  Cochran-Armitage  test  with  multiple  contrast  coefficients.  Statistical

significance is based on a p-value < 0.05.

**    The secondary efficacy analysis is a Cochran-Mantel-Haenszel (“CMH”) test stratified by baseline fibrosis stage for

Pairwise comparison of each OCA group compared to the placebo group. The multiplicity was not adjusted.

In the completer analysis, similar dose dependent effects were observed, with 51% of patients in the OCA 40 mg dose

group compared to 22% in the placebo group meeting the primary endpoint (p = 0.0061).

With the exception of dose dependent pruritus, OCA appeared to be generally safe and well tolerated. The number of
pruritus associated discontinuations were 0, 0, 2 and 5 patients in the placebo, OCA 10 mg, OCA 20 mg and OCA 40 mg
groups, respectively. Changes in lipid parameters, including LDL cholesterol, HDL cholesterol and triglycerides, appeared
to be consistent with previously reported lipid changes in Western NASH patients. No other meaningful differences in the
rate of adverse events between the OCA and placebo groups were noted.

Phase 2b FLINT Trial

In November 2014, the results from a Phase 2b clinical trial for the treatment of NASH, known as the FLINT trial,
which was sponsored by the NIDDK, a part of the National Institutes of Health, were published in The Lancet. The FLINT
trial was a double-blind, placebo-controlled trial of a once-daily dose of OCA 25 mg or placebo given for 72 weeks in 283
patients  with  biopsy-proven  NASH.  OCA  achieved  the  primary  endpoint  in  the  FLINT  trial,  which  was  defined  as  an
improvement of two or more points in NAS with no worsening of liver fibrosis.

The percentage of patients meeting the primary histological endpoint, based on liver biopsies, in the FLINT trial was
45% in the OCA treatment group and 21% in the placebo group (p = 0.0002, n = 219). The mean pre-treatment baseline
NAS for patients in the OCA treatment group was 5.3 of a total possible score of eight (comprised of a NAS of 0-2 for
hepatocellular  ballooning,  0-3  for  lobular  inflammation  and  0-3  for  steatosis).  Subgroup  analyses  showed  significant
response rates in the OCA treatment group in patients with risk factors for disease progression, including baseline fibrosis
stage,  co-morbid  type  2  diabetes  mellitus,  ALT,  insulin  resistance  and  severe  obesity  (each  factor  p  <  0.05  for  OCA
compared to placebo based on 95% confidence interval of published odds ratios).

A  significantly  greater  number  of  OCA-treated  patients  also  achieved  the  secondary  endpoint  of  improvement  of  at
least one fibrosis stage (35% versus 19%, p = 0.004), with OCA showing greater response rates as compared to placebo
across all stages of fibrosis. Based on our retrospective analyses of the FLINT data, more OCA-treated patients exhibited
fibrosis improvement of at least two fibrosis stages (15% versus 6%, not significant) and exhibited fibrosis improvements
regardless of baseline fibrosis stage and a significantly greater number of OCA-treated patients also achieved complete

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resolution of fibrosis (17% versus 5%, p = 0.0018). Also, our retrospective analysis of the FLINT data showed that fewer
OCA-treated patients progressed to bridging fibrosis (15% versus 18%, not significant) or to cirrhosis (2% versus 5%, not
significant). Retrospective analyses after the unblinding of results can potentially introduce bias and regulatory authorities
typically  give  greatest  weight  to  results  from  pre-specified  analyses  as  compared  to  retrospective  analyses.  The  NASH
Clinical  Research  Network  fibrosis  staging  system  was  used  to  categorize  the  pattern  of  fibrosis  and  architectural
remodeling  of  the  liver:  no  fibrosis  (F0),  perisinuoidal  or  periportal  fibrosis  (F1),  perisinusoidal  and  periportal  fibrosis
(F2), bridging fibrosis (F3) and cirrhosis (F4). Fibrosis sub-stages 1a, 1b and 1c were considered F1 for the analysis.

The  secondary  endpoint  of  NASH  resolution,  based  on  a  global  histological  assessment,  also  showed  improvement,
although  not  statistically  significant  (22%  versus  13%,  p  =  0.0832).  A  central  reading  of  all  baseline  and  end-of-trial
biopsies  was  performed  at  the  end  of  the  trial,  based  on  which  only  80%  of  patients  were  confirmed  to  have  definite
NASH,  while  the  remaining  20%  were  diagnosed  as  borderline  NASH  (10%)  or  not-NASH  (10%).  A  retrospective
subgroup  analysis  on  the  completer  population  comprised  only  of  definite  NASH  patients  at  baseline  showed  that  a
significantly  greater  number  of  OCA-treated  patients  achieved  NASH  resolution  compared  with  placebo-treated  patients
(19% versus 8%; p = 0.0278).

In an additional retrospective analysis of data from the FLINT trial conducted in a REGENERATE-matched patient
cohort published in 2018, (i) approximately 40% of OCA-treated patients as compared to approximately 21% of patients on
placebo  achieved  at  least  a  one-stage  improvement  in  liver  fibrosis  without  any  worsening  of  NASH  (p  =  0.02)  and  (ii)
approximately  20%  of  OCA-treated  patients  as  compared  to  approximately  7%  of  patients  on  placebo  achieved  NASH
resolution  with  no  worsening  of  fibrosis  (p  =  0.03)  using  the  definition  we  selected  for  NASH  resolution  in  the
REGENERATE trial.

In the FLINT trial, more OCA-treated patients experienced significant improvements in the major histological features
of  NASH,  including  steatosis  (61%  versus  38%,  p  =  0.001),  lobular  inflammation  (53%  versus  35%,  p  =  0.006)  and
hepatocellular ballooning (46% versus 31%, p = 0.03), as compared to the placebo treatment group. Trends were similar
between the two treatment groups for portal inflammation, which is not a component of NAS and is typically mild in adult
NASH patients.

The  histological  improvements  observed  in  OCA-treated  patients  versus  placebo  were  accompanied  by  statistically
significant reductions in relevant biochemical parameters, including the serum liver enzymes ALT (p < 0.0001), aspartate
aminotransferase (“AST”) (p = 0.0001) and gamma-glutamyl transferase (“GGT”) (p < 0.0001), each of which were above
generally accepted normal limits at baseline, and total bilirubin (p = 0.002). A modest but statistically significant increase
in ALP (p < 0.0001) in the OCA treatment group was also observed, but levels remained within typical normal limits.

OCA treatment was associated with serum lipid changes, including increases in total cholesterol and LDL cholesterol
and a decrease in HDL cholesterol, that developed within 12 weeks of treatment initiation, then reversed through the end of
treatment and returned to baseline during the 24-week post-treatment follow-up phase. Based on these observations, lipid
management was emphasized partway into the trial, using accepted guidelines. At 72 weeks as compared to baseline, the
following  effects  were  observed  in  the  OCA  treatment  group:  an  increase  in  mean  total  cholesterol  (0.16  mmol/L  or  6
mg/dL increase OCA versus 0.19 mmol/L or 7mg/dL decrease placebo, p = 0.0009), an increase in mean LDL cholesterol
(0.22 mmol/L or 9 mg/dL increase OCA versus 0.22 mmol/L or 8 mg/dL decrease placebo, p < 0.0001), a decrease in mean
HDL cholesterol (0.02 mmol/L or 1 mg/dL decrease OCA versus 0.03 mmol/L or 1 mg/dL increase placebo, p = 0.01) and
a decrease in triglycerides (0.22 mmol/L or 20 mg/dL decrease OCA versus 0.08 mmol/L or 7 mg/dL decrease placebo, p =
0.88,  not  significant).  These  changes  in  cholesterol  levels,  along  with  the  achievement  of  predefined  efficacy  criteria,
played a role in the decision of the FLINT data and safety monitoring board to terminate the treatment phase of the FLINT
trial, and the publication of the FLINT results noted the need for further study of these changes.

A post-hoc analysis showed OCA-treated patients who initiated statins during the FLINT trial (n = 26) experienced a
rapid  reversal  of  their  observed  mean  LDL  cholesterol  increase  to  below  baseline  levels,  with  a  mean  decrease  after  72
weeks of treatment of -18.9 mg/dL. In contrast, other OCA-treated patients with no reported initiation or change in statin
therapy experienced an increase in LDL cholesterol that peaked at week 12 and was sustained over the 72-week treatment
period.  Patients  treated  with  statins  at  baseline  who  maintained  statin  treatment  over  the  duration  of  the  study  (n  =  50)
experienced a mean LDL cholesterol increase of 8.7 mg/dL at 72 weeks. Patients not treated with statins during the study

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(n = 65) experienced a mean LDL cholesterol increase of 16.0 mg/dL. Treatment related LDL cholesterol increases in all
groups reversed with treatment discontinuation. This analysis suggests that the OCA-associated LDL cholesterol increase
reaches a maximum peak and plateaus soon after initiation of therapy and that concomitant statin use in NASH patients
receiving OCA may mitigate treatment-related LDL cholesterol increases.

In the FLINT trial, statistically significant weight loss of an average of 2.3 kilograms was observed in OCA patients
compared to no weight loss in the placebo group (p = 0.008), and this weight loss reverted towards baseline during the 24-
week follow-up phase. A pre-specified sensitivity analysis conducted by the investigators showed that weight loss was not
a  driver  of  the  primary  endpoint.  An  increase  in  a  marker  of  hepatic  insulin  resistance  known  as  homoeostasis  model
assessment  –  estimated  insulin  resistance  (“HOMA-IR”)  (calculated  using  the  product  of  fasting  plasma  insulin  and
glucose) was observed at 72 weeks in the OCA treatment group (p = 0.01). However, there was an imbalance in baseline
plasma insulin levels (201 pmol/L OCA versus 138 pmol/L placebo), and an even larger relative and absolute increase in
HOMA-IR  was  observed  in  the  placebo  group  at  the  conclusion  of  the  24-week  follow-up  phase.  This  is  potentially
attributable to the inherent variability in HOMA-IR measurements, particularly in patients with type 2 diabetes, that have
been  shown  to  make  single  time-point  to  time-point  changes  of  this  magnitude  clinically  uninterpretable.  There  were
virtually no changes in mean hemoglobin A1c, a measure of average blood sugar control over a period of approximately
three  months,  in  either  OCA  or  placebo  groups  at  72  weeks.  In  an  earlier  study  of  OCA  in  diabetic  NAFLD  patients
employing the hyperinsulinemic-euglycemic insulin clamp, the gold standard for detecting changes in insulin resistance,
OCA improved the glucose disposal rate consistent with reduced insulin resistance.

OCA was generally well tolerated in the FLINT trial. Adverse events were generally mild to moderate in severity and
the  incidence  in  the  OCA  and  placebo  treatment  groups  was  similar  for  all  symptoms  except  pruritus.  Pruritus  occurred
more frequently in the OCA treatment group than in the placebo treatment group (23% vs. 6%, p < 0.0001) and at a higher
grade (predominately moderate pruritus) but resulted in only one patient discontinuation. The incidence of severe or life-
threatening events was not different between the two treatment groups and most of the events in both groups were deemed
to be unrelated to treatment, including all severe or life-threatening cardiovascular events. There were two patient deaths in
the Phase 2b FLINT trial and neither death was considered related to OCA treatment.

OCA and Bezafibrate

In December 2018, we entered into an agreement (the “Aralez Agreement”) with Aralez Pharmaceuticals Canada Inc.
(“Aralez”),  pursuant  to  which  we  acquired  (i)  Aralez’s  license  to  develop  and  commercialize  bezafibrate  in  the  United
States (as amended and restated in connection therewith, the “Bezafibrate License”), (ii) Aralez’s IND on file with the FDA
and other associated regulatory documentation and (iii) a non-exclusive license to certain of Aralez’s intellectual property.
Pursuant  to  the  Aralez  Agreement,  we  paid  $9.0  million  to  Aralez  in  connection  with  the  closing  of  the  transactions  in
December 2018 and are obligated to make a $2.0 million milestone payment to Aralez based on the occurrence of specified
regulatory-related  events.  Pursuant  to  the  Bezafibrate  License,  we  are  also  obligated  to  make  a  $2.5  million  milestone
payment based on the occurrence of specified regulatory-related events with respect to such a combination product, as well
as mid-single digit percentage royalty payments based on the net sales of such a combination product.

Bezafibrate,  a  PPAR  agonist  that  has  been  studied  in  PBC,  is  not  approved  in  the  U.S.  for  any  indication.  We  are
evaluating the efficacy, safety and tolerability of OCA in combination with bezafibrate in patients with PBC in a Phase 2
study  outside  of  the  United  States.  In  the  United  States,  we  have  an  ongoing  Phase  1  study  to  better  characterize  the
exposure response of the fixed-dose combination, and we have an open IND application with the FDA. We are also in the
process of initiating a second Phase 2 study in the United States. Our longer-term goal is developing and seeking regulatory
approval for a fixed dose combination regimen in PBC and potentially in other diseases.

Other Product Candidates

The discovery and development of safe and effective new product candidates and the development of additional uses
for our existing product candidates and approved products, are important for the continued strength of our business. We,
together with our collaborators, have discovered several bile acid chemistry-based compounds that are in the early stages of
research and development. Among these compounds is INT-787, which is an FXR agonist that we are currently

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evaluating in a Phase 1 clinical trial. INT-787 has distinct pharmacological properties that differ from those of OCA and
has shown potential anti-fibrotic and anti-inflammatory effects in animal models. We believe that bile acid analogs may
have  utility  in  a  broad  range  of  diseases  beyond  non-viral  liver  disease  and  we  have  in  the  past,  and  may  in  the  future,
explore the potential application of our development compounds outside of our core areas of focus.

The  process  from  discovery  to  development  to  regulatory  approval  of  a  product  candidate  can  take  more  than  ten
years. Product candidates can fail at any stage of the process, and product candidates may not receive regulatory approval
even after many years of research and development and significant investment. In addition, we may decide to terminate or
deprioritize  the  development  of  our  product  candidates  due  to  a  number  of  factors,  including  our  views  of  the  relevant
regulatory  development  pathway,  competitive  landscape,  commercial  viability  of  the  product  candidate,  or  superior
alternative uses of capital. For example, we have studied OCA for PSC, a rare, serious, chronic cholestatic liver disease
characterized  by  a  progressive,  autoimmune-based  destruction  of  bile  ducts  with  eventual  onset  of  cirrhosis.  While  we
believe that the results of our Phase 2 AESOP trial announced in 2017 established a proof of concept of OCA in a second
cholestatic liver disease, we have deprioritized development of OCA in PSC based, in part, on the lack of clarity on the
regulatory pathway for this rare but serious disease. In addition, we are no longer actively developing INT-767, an orally
administered dual FXR and TGR5 agonist derived from the primary human bile acid chenodeoxycholic acid.

Competition

The  biotechnology  and  pharmaceutical  industries  are  intensely  competitive  and  subject  to  rapid  and  significant
technological  change.  We  have  competitors  in  the  United  States,  Europe  and  other  jurisdictions,  including  major
multinational pharmaceutical companies, established biotechnology companies, specialty pharmaceutical and generic drug
companies and universities and other research institutions. Many of our competitors have financial, sales and marketing,
manufacturing  and  distribution,  legal,  regulatory  and  product  development  resources  substantially  greater  than  ours.
Smaller  or  early-stage  companies  may  also  prove  to  be  significant  competitors,  particularly  through  collaborative
arrangements with large, established companies.

The ability of Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, and other future approved products,
if any, to compete with products sold by other companies will depend on a number of factors, including efficacy, safety and
tolerability, reliability, convenience of dosing, price, the level of branded and generic competition and reimbursement. We
believe that the competitive environment for Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH is as
follows.

Ocaliva for PBC

Ocaliva competes with UDCA (or ursodiol), a first-line therapy approved for the treatment of PBC that is available
generically  at  a  significantly  lower  cost  than  Ocaliva.  Additional  product  candidates  in  Phase  3  or  earlier  clinical  or
preclinical  development  for  the  treatment  of  PBC  include  Genfit  SA’s  dual  PPAR  alpha/delta  agonist  (elafibranor),
CymaBay’s  PPAR  delta  agonist  (seladelpar),  Genkyotex’s  NOX1/NOX4  inhibitor  (setanaxib),  HighTide’s  AMPK
activator/FXR agonist combination (HTD1801) and Fast Forward Pharmaceuticals BV’s anti-CD40 monoclonal antibody
(FFP104).  Additionally,  several  companies  have  product  candidates  aimed  at  the  cholestatic-induced  pruritus  associated
with  PBC,  including  apical  sodium  dependent  bile  acid  transport  inhibitors  being  developed  by  GlaxoSmithKline  plc
(GSK2330672).

Off-label uses of other potential treatments may also compete with Ocaliva for PBC. For example, while fibrates are
not approved for use in PBC, off-label use of fibrate drugs has been reported. Bezafibrate, a fibrate that is not approved by
the FDA for any indication and is only available outside of the United States, has been studied in PBC. Although we have a
license  to  develop  and  commercialize  bezafibrate  in  the  United  States,  bezafibrate  has  been  studied  in  multiple  clinical
trials for the treatment of liver diseases including PBC and NASH outside of the United States.

OCA for Liver Fibrosis Due to NASH

There are currently no medications approved for the treatment of NASH. However, various therapeutics are used off-

label for the treatment of NASH, including vitamin E (an antioxidant), insulin sensitizers (e.g., metformin, pioglitazone),

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antihyperlipidemic agents (e.g., gemfibrozil), pentoxifylline and UDCA. There are several product candidates in Phase 3 or
earlier  clinical  or  preclinical  development  for  the  treatment  of  NASH,  including  Madrigal  Pharmaceuticals,  Inc.’s  THR
beta agonist (resmetirom), Novo Nordisk’s GLP1 agonist (semaglutide), and Inventiva’s pan-PPAR agonist (lanifibranor),
as well as FXR agonists from Novartis AG (tropifexor, nidufexor), Metacrine (MET409, MET642), Terns Pharmaceuticals
(TERN-101), Gilead Sciences, Inc. (cilofexor) and Enanta Pharmaceuticals, Inc. (EDP-305).

Additional pharmaceutical and biotechnology companies with product candidates in development for the treatment of
NASH include AstraZeneca plc, Altimmune Inc., Boehringer Ingelheim GmbH, Bristol-Myers Squibb Company, Durect
Corporation,  Galectin  Therapeutics  Inc.,  Galmed  Pharmaceuticals  Ltd.,  Immuron  Ltd.,  Ionis  Pharmaceuticals,  Inc.,  Islet
Sciences, Inc., MediciNova, Inc., MiNA Therapeutics, NGM Biopharmaceuticals, Inc., NuSirt Sciences Inc., Pfizer Inc.,
Viking  Therapeutics,  Inc.  and  Zydus  Pharmaceuticals  (USA)  Inc.  NASH  is  a  complex  disease  and  we  believe  that  it  is
unlikely that any one therapeutic option will be optimal for every NASH patient.

In  addition,  many  universities  and  private  and  public  research  institutions  may  become  active  in  our  target  disease
areas. The results from our clinical trials and the approval of Ocaliva for PBC have brought more attention to our targeted
indications  and  bile  acid  chemistry.  As  a  result,  we  believe  that  additional  companies  and  organizations  may  seek  to
compete with us in the future. Our competitors may succeed in developing, acquiring or licensing on an exclusive basis,
technologies and drug products that are more effective or less costly than OCA or any other product candidates that we are
currently  developing  or  that  we  may  develop,  which  could  render  our  products  or  product  candidates  obsolete  and
noncompetitive. Our ability to compete may also be affected because, in many cases, insurers or other third-party payors
seek to encourage the use of generic products.

Intellectual Property

Protecting our intellectual property, such as our patents, is a key part of our strategy. We are the owner of record of
numerous  issued  U.S.  and  non-U.S.  patents  with  claims  directed  to  pharmaceutical  compounds,  pharmaceutical
compositions,  methods  of  making  these  compounds  and  methods  of  using  these  compounds  in  various  indications.  In
addition,  we  are  the  owner  of  record  of  numerous  pending  U.S.  and  non-U.S.  patent  applications,  and  regularly  pursue
additional patent applications in various jurisdictions. We also have numerous trademark and service mark registrations and
pending trademark and service mark applications in the United States and abroad.

The patent portfolio for OCA contains U.S. and non-U.S. patents and patent applications directed to compositions of
matter, methods of use and manufacturing methods. Our primary composition of matter patent for OCA was to expire in
2022. In light of the U.S. marketing approval of Ocaliva for PBC in May 2016, we applied for an extension of the patent
term for this patent in the United States into 2027, which extension has been granted. In addition, in connection with the
conditional approval of Ocaliva for PBC in the European Union, we have applied for supplementary protection certificates
(“SPC”) to extend the patent term for this patent in the European Union into 2027. To date, we have received grants of SPC
in  Austria,  Belgium,  Cyprus,  Denmark,  Finland,  France,  Germany,  Greece,  Ireland,  Italy,  Luxembourg,  Netherlands,
Norway,  Portugal,  Spain,  Sweden,  Switzerland  and  the  United  Kingdom  and  we  have  taken  similar  action  in  other
jurisdictions and countries where similar regulations exist. In February 2022, we filed a terminal disclaimer in the United
States  Patent  and  Trademark  Office  concerning  our  primary  composition  of  matter  patent  for  OCA,  which  changed  the
expiration date of the patent from November 16, 2027 to February 21, 2027.

The table set forth below summarizes the U.S. patents covering OCA that are listed in the FDA’s Orange Book List of
Approved  Drug  Products  with  Therapeutic  Equivalence  Evaluations  (the  “Orange  Book”).  The  issued  patents  covering
OCA are expected to expire in 2022 at the earliest and 2036 at the latest if the appropriate maintenance, renewal, annuity,
or other government fees are paid. We expect that the patents in the OCA portfolio that are listed in the Orange Book

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would expire as set forth below, assuming the appropriate maintenance, renewal, annuity or other governmental fees are
paid.

Patent No.
RE 48,286

8,058,267
8,377,916
9,238,673

Type of Patent(1)
  Composition of 

Matter

  Claims OCA compound

Brief Summary of Patent

  Method of Use
  Method of Use
  Composition of 

  Claims methods of treating PBC with OCA
  Claims methods of treating PBC with OCA
  Claims OCA active pharmaceutical ingredient 

Matter

(“API”)

10,047,117

  Method of Use

  Claims methods of treating FXR mediated

10,052,337

  Composition of 

  Claims OCA finished drug product

diseases with OCA API

Matter

U.S. Patent
Expiration
2027

2022
2022
2033

2033

2036

10,174,073

  Composition of

  Claims OCA API produced by a specified process  

2033

10,751,349

10,758,549

Matter
Composition of
Matter
Method of Use

Claims OCA finished drug product

Claims methods of treating PBC with OCA

2036

2036

(1) You should read the risk factors included elsewhere in this Annual Report on Form 10-K for important information
about  risks  posed  by  the  loss  of  patent  protection,  in  particular  the  risks  described  under  “Risk  Factors  —  Risks
Related to Our Intellectual Property.”

In addition, we have intellectual property protecting OCA that we would expect to list in the Orange Book if OCA is

approved for the treatment of NASH.

We  may  rely  on  trade  secrets  to  protect  our  proprietary  technologies,  especially  where  we  do  not  believe  patent
protection  is  appropriate  or  obtainable.  However,  trade  secrets  are  difficult  to  protect.  We  rely  in  part  on  confidentiality
agreements with our employees, consultants, outside scientific collaborators, sponsored researchers and other advisors to
protect our trade secrets and other proprietary information. We also seek to preserve the integrity and confidentiality of our
data, trade secrets and know-how by maintaining physical security of our premises and physical and electronic security of
our information technology systems.

Our commercial success will depend in part on our ability to obtain and maintain patent, trademark and trade secret
protection covering our products such as Ocaliva and product candidates, as well as our ability to successfully defend our
intellectual property against third-party challenges. Our ability to stop third parties from making, using, selling, offering to
sell  or  importing  our  products  is  dependent  upon  the  extent  to  which  we  have  regulatory  exclusivity  or  intellectual
property-based exclusivity rights under valid and enforceable patents or other intellectual property that cover our products.
If we fail to obtain and maintain adequate intellectual property protection, we may not be able to prevent third parties from
launching generic versions of our products, from using our proprietary technologies or from marketing products that are
very  similar  or  identical  to  ours.  The  patent  positions  of  pharmaceutical  companies  can  be  highly  uncertain  and  involve
complex legal and factual questions for which important legal principles remain unresolved. No consistent policy regarding
the breadth of claims allowed in pharmaceutical patents has emerged to date in the United States or in foreign jurisdictions,
and the legal standards relating to the patentability, validity and enforceability of pharmaceutical patents are evolving.

Changes in either the patent laws or in interpretations of patent laws in U.S. and foreign jurisdictions may diminish the
value of our intellectual property. Accordingly, we cannot predict the breadth of claims that may be enforced in the patents
that we currently own or that may issue from the applications we have filed or may file in the future or those that we may
license from third parties. Additionally, our currently pending or future patent applications may not result in issued patents,
and any term extensions that we seek may not be granted. Further, if any patents we obtain or license are deemed invalid or
unenforceable, it could impact our ability to commercialize or license our technology or enable third parties to develop and
market products that are similar or identical to ours.

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Manufacturing and Supply

We  do  not  own  or  operate  manufacturing  facilities  for  the  production  of  Ocaliva,  OCA  or  any  of  our  other  product
candidates, and we do not have any plans to develop our own manufacturing operations in the foreseeable future. We rely
on third-party contract manufacturers for all of our required raw materials, API and finished product for our commercial
sales and for our clinical trials and preclinical studies.

We  source  the  manufacture  and  commercial  supply  of  API  from  such  manufacturers,  for  use  in  Ocaliva  and,  if
approved, OCA for liver fibrosis due to NASH. We believe that we have secured supplies of API sufficient to meet our
PBC commercial supply requirements as well as our NASH commercial supply requirements during the initial stages of
our NASH launch if OCA is approved for the treatment of liver fibrosis due to NASH. One such supply agreement is with
PharmaZell  GmbH  (“PharmaZell”).  Our  supply  agreement  with  PharmaZell  does  not  require  us  to  purchase  a  specific
percentage  of  our  annual  commercial  requirements  of  API  from  PharmaZell.  We  have  also  qualified  an  additional  API
supplier from which we may currently acquire API on a purchase order basis and continue to engage in activities intended
to ensure that our long-term commercial supply requirements are satisfied. In connection with such efforts, we entered into
an agreement with a third potential supplier of API for the manufacture of Ocaliva and, if approved, OCA for liver fibrosis
due to NASH, under which we may in the future be obligated to purchase a portion of our API requirements in the event of
the achievement of agreed regulatory and product development milestones.

We do not have long-term supply agreements for any of our product candidates other than OCA, and regularly obtain
supplies and services relating to our product candidates from third-party contract manufacturers on a purchase order basis.
Contract manufacturers are subject to extensive governmental regulation and we depend on them for compliance with the
requirements of U.S. and non-U.S. regulators for the manufacture of our finished products, including Ocaliva. We intend to
continue  to  rely  on  third-party  manufacturers  for  the  manufacture  of  clinical  supplies  of  our  product  candidates  and
commercial supplies of our approved products, including Ocaliva and, if approved, OCA for liver fibrosis due to NASH.
We  believe  this  manufacturing  strategy  will  enable  us  to  direct  financial  resources  to  the  development  and
commercialization of products rather than diverting resources to establishing a manufacturing infrastructure.

Sales and Marketing

Ocaliva is our first approved product and the commercial launch of Ocaliva for PBC is our first product launch. We are
commercializing Ocaliva for PBC using a combination of our internal commercial organization and third-party distributors
depending on the jurisdiction. We are developing our commercialization strategy for OCA for liver fibrosis due to NASH,
if  approved,  and  have  not  yet  decided  on  our  commercialization  strategy  for  OCA  for  other  indications  or  for  our  other
product candidates, in each case, if approved. We intend to continue to evaluate how best to commercialize our product
candidates, if approved, in the United States and internationally, and may choose to collaborate with third parties that have
sales  and  marketing  capabilities  and  established  distribution  systems,  either  to  augment  our  own  capabilities  or  in  lieu
thereof.

Customers

We  commenced  our  commercial  launch  of  Ocaliva  for  the  treatment  of  PBC  in  the  United  States  in  June  2016.  In
December  2016,  the  European  Commission  granted  conditional  approval  for  Ocaliva  for  the  treatment  of  PBC  and  we
commenced our European (including United Kingdom) commercial launch in January 2017. Since January 2017, Ocaliva
has also received regulatory approval in several of our target markets outside the United States and Europe, including (but
not limited to) Canada, Israel and Australia. We recognized net product sales of Ocaliva of $363.5 million, $312.7 million
and  $249.6  million  for  the  years  ended  December  31,  2021,  2020  and  2019,  respectively.  We  sell  Ocaliva  to  a  limited
number of specialty pharmacies which dispense the product directly to patients. The specialty pharmacies are referred to as
our customers. For a discussion of our customer concentration, see Note 2 to our audited consolidated financial statements
included elsewhere in this Annual Report on Form 10-K.

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Government Regulation and Product Approval

Government  authorities  in  the  United  States,  at  the  federal,  state  and  local  level,  and  analogous  authorities  in  other
countries  extensively  regulate,  among  other  things,  the  research,  development,  testing,  manufacture,  recordkeeping,
approval, labeling, packaging, promotion, storage, advertising, distribution, marketing, sampling, post-approval monitoring
and reporting and export and import of products such as Ocaliva and those we are developing. Our product candidates must
be approved by the FDA through the NDA process before they may be legally marketed in the United States and by the
European  Commission  following  a  favorable  assessment  provided  by  the  EMA  through  the  MAA  process  for  a  product
falling  within  the  scope  of  the  Centralized  procedure  or  a  national  MAA  process  (albeit  through  the  process  of  Mutual
Recognition  or  Decentralized  procedure)  before  they  may  be  legally  marketed  in  the  European  Union.  Our  product
candidates will be subject to similar requirements in other countries prior to marketing in those countries. The process of
obtaining regulatory approvals and the subsequent compliance with applicable federal, state, local and foreign statutes and
regulations require the expenditure of substantial time and financial resources.

United States Government Regulation

NDA Approval Processes

In  the  United  States,  the  FDA  regulates  drugs  under  the  Federal  Food,  Drug,  and  Cosmetic  Act,  as  amended  (the
“FDCA”) and implementing regulations. An applicant seeking approval to market and distribute a new drug product in the
United States must typically undertake the following:

● completion of preclinical laboratory tests, animal studies and formulation studies in compliance with the FDA’s

good laboratory practice regulations;

● submission to the FDA of an IND, which must take effect before human clinical testing may begin;

● approval by an independent institutional review board (“IRB”), representing each clinical site before each clinical

trial may be initiated;

● performance  of  adequate  and  well-controlled  human  clinical  trials  in  accordance  with  good  clinical  practices
(“GCP”) to establish the safety and efficacy of the new drug product for each indication for which FDA approval
is sought;

● preparation and submission to the FDA of a NDA;

● review of the new drug product by an FDA advisory committee, where appropriate or if applicable, although the

FDA is not bound by the recommendation of an advisory committee;

● satisfactory completion of one or more FDA inspections of the manufacturing facility or facilities at which the
new drug product, or components thereof, are produced to assess compliance with current Good Manufacturing
Practices (“cGMP”) requirements and to assure that the facilities, methods and controls are adequate to preserve
the new drug product’s identity, strength, quality and purity;

● satisfactory completion of FDA audits of clinical trial sites to assure compliance with GCP and the integrity of

the clinical data;

● payment of user fees and procurement of FDA approval of the NDA; and

● compliance  with  any  post-approval  requirements,  including,  as  applicable,  Risk  Evaluation  and  Mitigation

Strategies (“REMS”) and post-approval studies required by the FDA.

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Preclinical and Clinical Studies

Once  a  pharmaceutical  candidate  is  identified  for  development,  it  enters  the  preclinical  or  nonclinical  testing  stage.
Nonclinical tests include laboratory evaluations of product chemistry, toxicity and formulation, as well as animal studies.
An IND sponsor must submit the results of the nonclinical tests, together with manufacturing information and analytical
data, to the FDA as part of the IND. Some nonclinical testing may continue even after the IND is submitted. In order to
conduct  clinical  research,  an  IND  sponsor  must  submit  an  IND.  An  IND  automatically  becomes  effective  30  days  after
receipt by the FDA, unless the FDA, within the 30-day time period, or any time thereafter, places the IND on clinical hold.
In  such  a  case,  the  IND  sponsor  and  the  FDA  must  resolve  any  outstanding  concerns  before  clinical  trials  can  begin  or
continue. A clinical hold may affect one or more specific studies or all studies conducted under the IND.

All clinical trials must be conducted under the supervision of one or more qualified investigators in accordance with
GCPs.  They  must  be  conducted  under  protocols  detailing  the  objectives  of  the  trial,  dosing  procedures,  research  subject
selection and exclusion criteria and the safety and effectiveness criteria to be evaluated. Each protocol must be submitted to
the FDA as part of the IND, and progress reports detailing the status of the clinical trials must be submitted to the FDA
annually. Sponsors also must timely report to the FDA serious and unexpected adverse reactions, any clinically important
increase in the rate of a serious suspected adverse reaction over that listed in the protocol or investigation brochure, or any
findings from other studies or animal or in vitro testing that suggest a significant risk in humans exposed to the drug. An
IRB at each institution must, among other things, review and approve the protocol before a clinical trial commences at such
institution,  and  approve  the  consent  form  that  must  be  provided  to  each  research  subject  or  the  subject’s  legal
representative, monitor the study until completed and otherwise comply with regulations applicable to the IRB.

Human  clinical  trials  are  typically  conducted  in  three  sequential  phases,  although  the  phases  may  overlap  or  be

combined:

● Phase  1.  The  drug  is  initially  introduced  into  healthy  human  subjects  and  tested  to  assess  pharmacological
actions, safety, dosage tolerance, absorption, metabolism, distribution and elimination and, in some cases, early
evidence  of  effectiveness.  In  the  case  of  some  products  intended  for  the  treatment  of  severe  or  life-threatening
diseases,  such  as  cancer,  especially  when  the  product  may  be  inherently  too  toxic  to  ethically  administer  to
healthy volunteers, the initial human testing is often conducted in patients.

● Phase 2. Clinical trials are performed on a limited patient population intended to identify possible adverse effects
and  safety  risks,  to  preliminarily  evaluate  the  efficacy  of  the  product  for  specific  targeted  diseases  and  to
determine dosage tolerance and optimal dosage.

● Phase 3.  Clinical  trials  are  undertaken  to  further  evaluate  dosage,  clinical  efficacy  and  safety  in  an  expanded
patient  population  generally  at  geographically  dispersed  clinical  study  sites.  These  studies  are  intended  to
establish the overall risk-benefit ratio of the product and provide an adequate basis for product labeling, should it
ultimately be approved for marketing. In most cases the FDA requires two adequate and well-controlled Phase 3
clinical trials with statistically significant results to demonstrate the efficacy of the drug. A single Phase 3 clinical
trial with other confirmatory evidence may be sufficient in certain instances.

Human  clinical  trials  are  inherently  uncertain  and  Phase  1,  Phase  2  and  Phase  3  testing  may  not  be  successfully
completed. The FDA or the sponsor may suspend a clinical trial at any time for a variety of reasons, including a finding
that the research subjects or patients are being exposed to an unacceptable health risk. Similarly, an IRB can suspend or
terminate approval of a clinical trial at its institution if the clinical trial is not being conducted in accordance with the IRB’s
requirements or if the drug has been associated with unexpected serious harm to patients. In some cases, clinical trials are
overseen by an independent group of qualified experts organized by the trial sponsor, or the clinical monitoring board or
data monitoring committee. This group typically provides recommendations to the trial sponsor for whether or not a trial
may move forward at designated check points. These decisions are based on the data monitoring committee’s independent
review of data from the ongoing trial.

Sponsors of clinical trials of certain FDA-regulated products, including prescription drugs, are required to register and

disclose clinical trial information related to the product, patient population, phase of investigation, clinical trial sites and

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investigator, and other aspects of the clinical trial on a public website maintained by the U.S. National Institutes of Health.
Sponsors  are  also  obligated  to  disclose  the  results  of  these  clinical  trials  after  completion.  For  a  new  product  or  a  new
indication for a previously approved product, sponsors can delay submission of clinical study results for up to two years
until the product has been approved or approved for the new use. Competitors and others may use this publicly-available
information to gain knowledge regarding the design and progress of our development programs.

During  the  development  of  a  new  drug,  sponsors  are  given  opportunities  to  meet  with  the  FDA  at  certain  points,
including prior to the submission of an IND, at the end of Phase 2 and before a NDA is submitted. Meetings at other times
may be requested. These meetings can provide an opportunity for the sponsor to share information about the data gathered
to  date  and  for  the  FDA  to  provide  advice  and  feedback  on  the  next  phase  of  development.  Sponsors  typically  use  the
meeting at the end of Phase 2 to discuss their Phase 2 clinical results and present their plans for the pivotal Phase 3 clinical
trial(s) that they believe will support the approval of the new drug. If a Phase 2 clinical trial is the subject of discussion at
the end of Phase 2 meeting with the FDA, a sponsor may be able to request a special protocol assessment (“SPA”), the
purpose of which is to reach agreement with the FDA on the Phase 3 clinical trial protocol design and analysis that will
form the primary basis of an efficacy claim.

Concurrent with clinical trials, sponsors usually complete additional animal safety studies and also develop additional
information  about  the  chemistry  and  physical  characteristics  of  the  drug  and  finalize  a  process  for  manufacturing
commercial quantities of the product in accordance with cGMP requirements. The manufacturing process must be capable
of consistently producing quality batches of the drug and the manufacturer must develop methods for testing the quality,
purity  and  potency  of  the  drug  prior  to  release.  Additionally,  appropriate  packaging  must  be  selected  and  tested  and
stability  studies  must  be  conducted  to  demonstrate  that  the  drug  candidate  does  not  undergo  unacceptable  deterioration
over its proposed shelf-life.

The  results  of  product  development,  nonclinical  studies  and  clinical  trials,  along  with  descriptions  of  the
manufacturing process, analytical tests and other control mechanisms, proposed labeling and other relevant information are
submitted to the FDA as part of a NDA requesting approval to market the product. The submission of a NDA is subject to
the  payment  of  user  fees,  but  a  waiver  of  such  fees  may  be  obtained  under  specified  circumstances.  Currently,  the
application  fee  is  approximately  $3.1  million  for  NDAs  with  clinical  data  and  approximately  $1.6  million  for  NDAs
without  clinical  data.  The  sponsor  under  an  approved  NDA  is  also  subject  to  annual  program  user  fees,  currently
approximately $369,000. Program fees are assessed for each approved prescription drug product identified in an approved
application,  up  to  five  program  fees  per  application.  These  fees  are  typically  modified  annually.  The  FDA  reviews  all
NDAs submitted to ensure that they are sufficiently complete for substantive review before it accepts them for filing. It
may request additional information rather than accept a NDA for filing. In this event, the NDA must be resubmitted with
the additional information. The resubmitted application also is subject to review before the FDA accepts it for filing.

Once  the  NDA  is  accepted  for  filing,  the  FDA  begins  an  in-depth  review.  NDAs  receive  either  standard  or,  as
discussed more fully below, priority review. The FDA may refuse to approve a NDA if the applicable regulatory criteria are
not  satisfied  or  may  require  additional  clinical  or  other  data.  Even  if  such  data  are  submitted,  the  FDA  may  ultimately
decide that the NDA does not satisfy the criteria for approval. The FDA reviews a NDA to determine, among other things,
whether a product is safe, effective, and can be properly manufactured for its intended use or uses. The FDA may refer the
NDA  to  an  advisory  committee  for  review  and  recommendation  as  to  whether  the  application  should  be  approved  and
under what conditions. The FDA is not bound by the recommendation of an advisory committee. Before approving a NDA,
the  FDA  will  inspect  the  facility  or  facilities  where  the  product  is  manufactured  and  tested  to  ensure  compliance  with
cGMPs.  An  approval  letter  from  the  FDA  authorizes  commercial  marketing  of  the  product  and  specifies  the  prescribing
information for the approved indication(s).

Fast Track, Breakthrough Therapy, Priority Review and Accelerated Approval

The  FDA  is  authorized  to  designate  certain  products  for  expedited  review  if  they  are  intended  to  address  an  unmet
medical  need  in  the  treatment  of  a  serious  or  life-threatening  disease  or  condition.  These  programs  include  fast  track
designation, breakthrough therapy designation and priority review designation.

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Specifically, the FDA may designate a product for fast track review if it is intended, whether alone or in combination
with one or more other drugs, for the treatment of a serious or life-threatening disease or condition, and it demonstrates the
potential to address unmet medical needs for such a disease or condition. For fast track designated products, sponsors may
have a higher number of interactions with the FDA and the FDA may initiate review of sections of a fast track product’s
NDA before the application is complete.

A product may also be designated as a breakthrough therapy if it is intended, either alone or in combination with one
or more other drugs, to treat a serious or life-threatening disease or condition and preliminary clinical evidence indicates
that  the  product  may  demonstrate  substantial  improvement  over  existing  therapies  on  one  or  more  clinically  significant
endpoints, such as substantial treatment effects observed early in clinical development. The FDA may take certain actions
with respect to breakthrough therapies, including holding meetings with the sponsor throughout the development process;
providing  timely  advice  to  the  product  sponsor  regarding  development  and  approval;  involving  more  senior  staff  in  the
review process; assigning a cross-disciplinary project lead for the review team; and taking other steps to design the clinical
trials in an efficient manner.

The FDA may also designate a product for priority review if it would provide a significant improvement in the safety
or effectiveness of the treatment, diagnosis or prevention of a serious condition. Certain other applications may also qualify
for  priority  review.  The  FDA  determines,  on  a  case-by-case  basis,  whether  the  proposed  drug  represents  a  significant
improvement when compared with other available therapies. A priority designation by the FDA is intended to direct the
agency’s attention and resources to the evaluation of such applications, and to shorten the FDA’s goal for taking action on a
marketing application from ten months to six months.

In addition, the FDA may grant accelerated approval to a drug for a serious or life-threatening condition that provides
meaningful  therapeutic  advantage  to  patients  over  existing  treatments  based  upon  a  determination  that  the  drug  has  an
effect  on  a  surrogate  endpoint  that  is  reasonably  likely  to  predict  clinical  benefit.  The  FDA  may  also  grant  accelerated
approval  for  such  a  condition  when  the  product  has  an  effect  on  an  intermediate  clinical  endpoint  that  can  be  measured
earlier than an effect on irreversible morbidity or mortality, and that is reasonably likely to predict an effect on irreversible
morbidity or mortality or other clinical benefit, taking into account the severity, rarity, or prevalence of the condition and
the  availability  or  lack  of  alternative  treatments.  Drugs  granted  accelerated  approval  must  meet  the  same  statutory
standards  for  safety  and  effectiveness  as  those  granted  traditional  approval.  In  the  case  of  unprecedented  accelerated
approval endpoints, this determination occurs during the review of the NDA. Unless otherwise informed by the FDA, an
applicant  must  submit  to  the  FDA  for  consideration  during  the  preapproval  review  period  copies  of  all  promotional
materials, including promotional labeling as well as advertisements, intended for dissemination or publication within 120
days following marketing approval. After 120 days following marketing approval, unless otherwise informed by the FDA,
the applicant must submit promotional materials at least 30 days prior to the intended time of initial dissemination of the
labeling or initial publication of the advertisement.

As  a  condition  of  a  grant  of  accelerated  approval,  the  FDA  may  require  that  the  sponsor  perform  one  or  more
controlled post-marketing clinical trials. Approval of a drug may be withdrawn if these trials fail to verify clinical benefit
or  do  not  demonstrate  sufficient  clinical  benefit  to  justify  the  risks  associated  with  the  drug  (e.g.,  show  a  significantly
smaller magnitude or duration of benefit than was anticipated based on the observed effect on the surrogate).

See “Item 1. Business—Overview” for discussion of our accelerated approval status.

Post-approval Requirements

Drugs manufactured or distributed pursuant to FDA approvals are subject to pervasive and continuing regulation by
the FDA post-approval, including, among other things, requirements relating to recordkeeping, periodic reporting, product
sampling  and  distribution,  advertising  and  promotion  and  reporting  of  adverse  experiences  with  the  product.  Once  an
approval is granted, the FDA may withdraw the approval if compliance with regulatory requirements is not maintained or
if safety or other problems occur after the product reaches the market. Later discovery of previously unknown problems
with a product may result in new labeling information (e.g., warnings), customer training and/or education requirements,
restrictions  on  the  product  or  even  complete  withdrawal  of  the  product  from  the  market.  After  approval,  some  types  of
changes to the approved product, such as adding new indications, manufacturing changes and additional labeling claims,

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are subject to further FDA review and approval. In addition, the FDA may require studies, trials, analyses, and surveillance
programs  to  monitor  or  evaluate  the  effect  of  approved  products  that  have  been  commercialized,  and  the  FDA  has  the
power to limit further marketing of a product, or seek withdrawal of approval, based on the results of these post-marketing
programs.

Drug manufacturers and other entities involved in the manufacture and distribution of approved drugs are required to
register their establishments with the FDA and certain state agencies, and are subject to periodic unannounced inspections
by the FDA and some state agencies for compliance with cGMP and other laws. Changes to the manufacturing process are
strictly  regulated  and  often  require  prior  FDA  approval  before  being  implemented.  FDA  regulations  also  require
investigation and correction of any deviations from cGMP and impose reporting and documentation requirements upon the
sponsor and any third-party manufacturers that the sponsor may decide to use. Accordingly, manufacturers must continue
to expend time, money, and effort in the area of production and quality control to maintain cGMP compliance.

Failure  to  comply  with  the  applicable  U.S.  requirements  at  any  time  during  the  product  development  process  or
approval process, or after approval, may subject us to judicial, regulatory or statutory sanctions, any of which could have a
material adverse effect on us.

These sanctions could include:

● refusal to approve pending applications;

● withdrawal of an approval;

● imposition of a clinical hold;

● warning or untitled letters;

● product recalls;

● product seizures;

● total or partial suspension of production or distribution; and

● injunctions, fines, disgorgement, civil penalties and criminal prosecution.

The  FDA  and  other  U.S.  state  and  federal  authorities  regulate  marketing,  labeling,  advertising  and  promotion  of
products  that  are  placed  on  the  market.  Drugs  may  be  promoted  only  for  the  approved  indications  and  in  a  manner
otherwise  consistent  with  the  provisions  of  the  approved  label  and  FDA  regulations.  The  FDA  and  other  authorities
actively  enforce  the  laws  and  regulations  prohibiting  false,  misleading,  deceptive,  or  off-label  promotional  practices;
violations of these prohibitions can lead to significant liability. Additional regulations apply for advertising and promotion
of  products  approved  under  the  accelerated  approval  pathway.  For  example,  unless  otherwise  informed  by  the  FDA,  an
applicant  must  submit  to  the  FDA  for  consideration  during  the  preapproval  review  period  copies  of  all  promotional
materials, including promotional labeling as well as advertisements, intended for dissemination or publication within 120
days following marketing approval. After 120 days following marketing approval, unless otherwise informed by the FDA,
the applicant must submit promotional materials at least 30 days prior to the intended time of initial dissemination of the
labeling or initial publication of the advertisement.

We rely, and expect to continue to rely, on third parties for the production of clinical and commercial quantities of our
products. Future FDA and state inspections may identify compliance issues at the facilities of our contract manufacturers
that may disrupt production or distribution, or require substantial resources to correct.

From  time  to  time,  legislation  is  introduced  and  passed  in  Congress  that  could  significantly  change  the  statutory
provisions  governing  the  approval,  manufacturing  and  marketing  of  products  regulated  by  the  FDA.  In  addition,  FDA
regulations and guidance are often revised or reinterpreted by the agency in ways that may significantly affect our business

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and our products. It is impossible to predict whether legislative changes will be enacted, or FDA regulations, guidance or
interpretations changed or what the impact of such changes, if any, may be.

In  accordance  with  the  applicable  requirements  under  the  accelerated  approval  pathway,  we  initiated  our  Phase  4
COBALT clinical outcomes confirmatory trial for Ocaliva in PBC in December 2014, following discussions with the FDA.
The study was designed to evaluate subjects across the spectrum of PBC disease, including early and advanced PBC. We
also agreed to evaluate the safety and efficacy of Ocaliva in patients with moderate to severe hepatic impairment in a study
known  as  the  401  trial  and  as  monotherapy  in  patients  with  PBC.  In  addition,  we  agreed  to  develop  and  characterize  a
lower  dose  formulation  of  Ocaliva  to  allow  for  once  daily  dosing  in  patients  with  moderate  or  advanced  hepatic
impairment.

Risk Evaluation and Mitigation Strategy

The Food and Drug Administration Amendments Act of 2007 created a new section of the FDCA which authorizes the
FDA to require a REMS as a condition of NDA approval, or based upon new safety information regarding an approved
drug, when the FDA determines a REMS is necessary to ensure that the benefits of a drug outweigh the potential risks.
Under  a  REMS,  the  FDA  may  require  various  measures  to  address  serious  risks,  such  as  medication  guides,
communication plans, training or registries, as well as steps to monitor and assess the effectiveness of those measures. Such
requirements may impose significant burdens on prescribers, pharmacists or patients. The requirement for a REMS may
materially affect the potential market and profitability of a drug.

We do not have a REMS for Ocaliva for the treatment of PBC.

Patent Term Extension and Data Exclusivity

Depending upon the timing, duration and specifics of FDA approval of the use of our drug candidates, some of our
U.S.  patents  may  be  eligible  for  limited  patent  term  extension  under  the  Drug  Price  Competition  and  Patent  Term
Restoration Act of 1984, (the “Hatch-Waxman Act”). The Hatch-Waxman Act permits an extension of a patent term of up
to  five  years  as  compensation  for  patent  term  lost  during  product  development  and  the  FDA  regulatory  review  process.
However, the extension of patent term cannot extend the remaining term of a patent beyond a total of 14 years from the
product’s approval date. The patent term extension period is generally one-half the time between the effective date of an
IND, and the submission date of a NDA, plus the time between the submission date of a NDA and the approval of that
application. Only one patent applicable to an approved drug is eligible for the extension and the application for extension
must be made prior to expiration of the patent. The United States Patent and Trademark Office, in consultation with the
FDA, reviews and approves the application for any patent term extension or restoration.

Data exclusivity provisions under the FDCA also can delay the submission or the approval of certain applications. The
FDCA  provides  a  five-year  period  of  non-patent  data  exclusivity  within  the  United  States  to  the  first  applicant  to  gain
approval of a NDA for a new chemical entity. A drug is considered a new chemical entity if the FDA has not previously
approved any other new drug containing the same active moiety, which is the molecule or ion responsible for the action of
the  drug  substance  as  further  defined  in  FDA  regulations.  During  the  exclusivity  period,  the  FDA  may  not  accept  for
review  an  abbreviated  new  drug  application  (“ANDA”)  or  a  505(b)(2)  NDA  for  a  drug  with  the  same  active  moiety.
However,  an  application  may  be  submitted  four  years  from  the  NDA  approval  date  if  it  contains  a  paragraph  IV
certification that a reference product patent is invalid or not infringed by the ANDA or 505(b)(2) product. The FDCA also
provides  three  years  of  marketing  exclusivity  for  a  NDA,  505(b)(2)  NDA  or  supplement  to  an  approved  NDA  if  new
clinical investigations, other than bioavailability studies, that were conducted or sponsored by the applicant are deemed by
the  FDA  to  be  essential  to  the  approval  of  the  application,  for  example,  for  new  indications,  dosages  or  strengths  of  an
existing  drug.  This  three-year  exclusivity  covers  only  the  conditions  associated  with  the  new  clinical  investigations  and
does not prohibit the FDA from approving ANDAs or 505(b)(2) NDAs for drugs containing the original active moiety for
other  conditions  of  use.  Five-year  and  three-year  exclusivity  will  not  delay  the  submission  or  approval  of  a  full  NDA;
however,  an  applicant  submitting  a  full  NDA  may  be  required  to  conduct  or  obtain  a  right  of  reference  to  all  of  the
preclinical studies and adequate and well-controlled clinical trials necessary to demonstrate safety and effectiveness.

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Pediatric Exclusivity and Pediatric Use

In the United States, under the Best Pharmaceuticals for Children Act, sponsors may obtain a six month extension of
unexpired  regulatory  exclusivities  and  terms  of  unexpired  Orange  Book-listed  patents  relating  to  their  drug,  if  pediatric
studies substantially complying with a Written Request are completed and submitted by the sponsor to the FDA within the
statutory time frame. In December 2021, we submitted a request to the FDA seeking a Written Request for pediatric studies
concerning obeticholic acid.

In  addition,  in  Canada,  in  September  2021,  we  submitted  materials  to  Health  Canada,  the  applicable  regulator,
regarding  pediatric  study  information  and  pediatric  labeling,  which  could  result  in  a  six-month  market  exclusivity
extension in Canada.

In addition, under the Pediatric Research Equity Act (the “PREA”), a NDA or supplement to a NDA for certain drugs
must  contain  data  to  assess  the  safety  and  effectiveness  of  the  drug  for  the  claimed  indications  in  all  relevant  pediatric
subpopulations and to support dosing and administration for each pediatric subpopulation for which the product is safe and
effective,  unless  the  sponsor  receives  a  deferral  or  waiver.  The  FDA  has  recently  issued  guidance  limiting  a  sponsor’s
ability to waive the PREA study requirements.

Orphan Drug Designation

Under the Orphan Drug Act, the FDA may grant orphan drug designation to drugs intended to treat a rare disease or
condition,  which  is  generally  a  disease  or  condition  that  affects  fewer  than  200,000  individuals  in  the  United  States,  or
more  than  200,000  individuals  in  the  United  States  and  for  which  there  is  no  reasonable  expectation  that  the  cost  of
developing and making available in the United States a drug for this type of disease or condition will be recovered from
sales in the United States for that drug. Orphan drug designation must be requested before submitting a NDA. After the
FDA  grants  orphan  drug  designation,  the  identity  of  the  therapeutic  agent  and  its  potential  orphan  use  are  disclosed
publicly by the FDA. Orphan drug designation does not convey any advantage in or shorten the duration of the regulatory
review and approval process.

If a product that has orphan drug designation subsequently receives the first FDA approval for the disease for which it
has such designation, the product is entitled to orphan drug exclusivity, which means that the FDA may not approve any
applications from any other party to market the same drug for the same indication for seven years, except in very limited
circumstances such as where there is a demonstration of clinical superiority. Orphan drug exclusivity, however, could also
work to block the approval of one of our product candidates for seven years if a competitor develops the same drug as one
of  our  product  candidates  and  obtains  approval  and  orphan  exclusivity  for  the  same  indication  or  disease  for  which  our
product candidate is being developed. Orphan drug exclusivity would not block approval of the same drug developed by a
competitor for a use different from our orphan-protected approved use. If a drug or drug product designated as an orphan
product ultimately receives marketing approval for an indication broader than what was designated in its orphan product
application, it may not be entitled to orphan exclusivity for the full scope of its approved use.

As in the United States, we may apply for designation of a product as an orphan drug for the treatment of a specific
indication in the European Union before the application for marketing authorization is made. Orphan drugs in Europe enjoy
economic and marketing benefits, including up to ten years of market exclusivity for the approved indication. The market
exclusivity period for the authorized therapeutic indication may be reduced to six years if, at the end of the fifth year, it is
established  that  the  orphan  designation  criteria  are  no  longer  met,  including  where  it  is  shown  that  the  product  is
sufficiently profitable not to justify maintenance of market exclusivity. In addition, a competing similar medicinal product
may in limited circumstances be authorized prior to the expiration of the market exclusivity period, including if it is shown
to be safer, more effective or otherwise clinically superior to the orphan-designated product.

OCA has received orphan drug designation in the United States and the European Union for the treatment of PBC and

PSC. In the United States, Ocaliva’s orphan exclusivity for its approved PBC indication runs until May 27, 2023.

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Regulation Outside of the United States

In addition to regulations in the United States, we are subject to regulations of other countries governing clinical trials
and  commercial  sales  and  distribution  of  our  products.  Whether  or  not  we  obtain  FDA  approval  for  a  product,  we  must
obtain approval by the comparable regulatory authorities of countries outside of the United States before we can commence
clinical trials in such countries and approval of the regulators of such countries or economic areas, such as the European
Union, before we may market products in those countries or areas. The approval process and requirements governing the
conduct of clinical trials, product licensing, pricing and reimbursement vary greatly from place to place, and the time may
be longer or shorter than that required for FDA approval.

Under  European  Union  regulatory  systems,  a  company  may  submit  marketing  authorization  applications  under  the
centralized, decentralized or mutual recognition marketing authorization procedure. The centralized procedure provides for
the  grant  of  a  single  marketing  authorization  for  a  medicinal  product  by  the  European  Commission  on  the  basis  of  an
opinion provided by the EMA’s Committee for Medicinal Products for Human Use (the “CHMP”). A centralized marketing
authorization  is  valid  for  all  European  Union  member  states  and  the  European  Economic  Area  States  (Iceland,
Liechtenstein and Norway). The decentralized marketing authorization procedure involves the submission of an application
for  marketing  authorization  to  the  competent  authorities  in  each  of  the  European  Union  member  states  chosen  by  the
applicant in which the product is to be marketed. One national competent authority, selected by the applicant (Reference
Member State) leads the assessment of the application for marketing authorization. The competent authorities of the other
chosen European Union member states concerned by the procedure (Concerned Member States) are subsequently required
to review the initial evaluation and, if the assessment is positive and all issues are resolved, grant marketing authorization
for their territory on the basis of the assessment, except where grounds of potential serious risk to public health require the
application  for  authorization  to  be  refused.  The  mutual  recognition  procedure  provides  for  mutual  recognition  of  a
marketing authorization which has already been granted by the national competent authority of a European Union member
state by the competent authorities of the other European Union member states where further marketing authorizations are
progressively  sought.  The  holder  of  a  national  marketing  authorization  may  submit  an  application  to  the  competent
authority  of  a  European  Union  member  state  requesting  the  recognition  of  the  marketing  authorization  granted  by  the
competent authority of another European Union member state.

Prior to obtaining a marketing authorization in the European Union submitted as a full stand-alone dossier, applicants
have to demonstrate compliance with all measures included in an EMA-approved PIP covering all subsets of the pediatric
population, unless the EMA has granted (1) a product-specific waiver, (2) a class waiver, or (3) a deferral for one or more
of the measures included in the PIP. In the case of orphan medicinal products, completion of an approved PIP can result in
an extension of the aforementioned market exclusivity period from ten to twelve years.

It  is  also  possible  that  a  centralized  marketing  authorization  could  be  conditional  on  post-approval  studies  and  not
considered a full approval, but subject to annual renewal until comprehensive data are provided to confirm the benefit/risk
assessment.  A  manufacturer’s  ability  to  obtain  and  maintain  conditional  marketing  authorization  in  the  European  Union
will be limited to specific circumstances and subject to several conditions and obligations, if obtained at all. Conditional
marketing  authorizations  can  be  granted,  based  on  a  clinical  dataset  that  is  not  comprehensive.  Granting  of  such  an
authorization  may  be  granted  for  a  limited  number  of  medicinal  products  for  human  use  referenced  in  the  applicable
European  Union  law  governing  conditional  marketing  authorization,  including  products  designated  as  orphan  medicinal
products  under  European  Union  law,  if  (1)  the  risk-benefit  balance  of  the  product  is  positive,  (2)  it  is  likely  that  the
applicant will be in a position to provide the required comprehensive clinical trial data, (3) unmet medical needs will be
fulfilled and (4) the benefit to public health of the immediate availability on the market of the medicinal product outweighs
the  risk  inherent  in  the  fact  that  additional  data  are  still  required.  Specific  obligations,  including  with  respect  to  the
completion of ongoing or new studies, and with respect to the collection of pharmacovigilance data, may be specified in
the conditional marketing authorization. Conditional marketing authorizations are valid for one year, and may be renewed
annually,  if  the  risk-benefit  balance  remains  positive,  and  after  an  assessment  of  the  need  for  additional  or  modified
conditions.

Similarly  to  the  United  States,  both  marketing  authorization  holders  and  manufacturers  of  medicinal  products  are
subject to comprehensive regulatory oversight by the EMA and the competent authorities of the individual European Union
member states both before and after grant of the manufacturing and marketing authorizations. This includes European

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Union  cGMP  rules,  which  govern  quality  control  of  the  manufacturing  process  and  require  documentation  policies  and
procedures. We and our third-party manufacturers are required to ensure that all of our processes, methods, and equipment
are compliant with cGMP.

Failure by us or by any of our third-party partners, including suppliers, manufacturers, and distributors to comply with
European Union laws and the related national laws of individual European Union member states governing the conduct of
clinical trials, manufacturing approval, marketing authorization of medicinal products and manufacturing and marketing of
such  products,  both  before  and  after  grant  of  marketing  authorization,  may  result  in  administrative,  civil  or  criminal
penalties.  These  penalties  could  include  delays  in  or  refusals  to  authorize  the  conduct  of  clinical  trials  or  the  grant  of
marketing  authorizations,  product  withdrawals  and  recalls,  product  seizures,  suspensions,  withdrawals,  or  variations  of
previously  granted  marketing  authorizations,  total  or  partial  suspensions  of  production,  distribution,  manufacturing,  or
clinical trials, operating restrictions, injunctions, suspension of licenses, fines and criminal penalties.

In  October  2016,  the  CHMP  of  the  EMA  adopted  a  positive  opinion  recommending  the  granting  of  a  conditional
marketing authorization of Ocaliva in PBC. Based on the CHMP’s positive recommendation, the European Commission
granted  a  conditional  marketing  authorization  of  Ocaliva  in  PBC  in  December  2016.  Although  we  have  successfully
renewed our conditional marketing authorization in the European Union in the past, there can be no assurance that we will
be able to continue to do so in the future. Failure to renew our conditional marketing authorization would prevent us from
continuing  to  market  Ocaliva  for  PBC  in  Europe.  PBC  is  extremely  rare  in  the  pediatric  population.  Therefore,  in
accordance  with  applicable  regulations,  the  PBC  marketing  authorization  required  demonstration  of  compliance  with  all
measures  included  in  an  EMA-approved  Pediatric  Investigation  Plan  for  OCA  for  the  treatment  of  biliary  atresia,  a
pediatric cholestatic disease.

Pricing and Reimbursement

Sales of our products will depend, in part, on the extent to which the costs of our products will be covered by third-
party payors, such as government healthcare programs, commercial insurance plans and managed healthcare organizations.
These third-party payors are increasingly challenging the prices charged for medical products and services. Additionally,
the containment of healthcare costs has become a priority for federal and state governments and the prices of drugs have
been a focus in this effort. The U.S. government, state legislatures and foreign governments have shown significant interest
in implementing cost-containment programs, including price controls, restrictions on reimbursement and requirements for
substitution of generic products. Adoption of new or more restrictive price controls and cost-containment measures in the
jurisdictions in which we operate could materially and adversely impact our net sales and financial results.

Third-party  payers  are  responsible  for  managing  overall  pharmaceutical  drug  spending  for  their  client  membership.
Third-party  payers  continue  to  scrutinize  and  manage  the  prices  charged  for  pharmaceutical  products  and  services,  and
many also limit reimbursement for newly-approved or innovating products and indications. If these third-party payors do
not consider our products to be cost-effective compared to other therapies, they may (i) not cover our approved products as
part of their plans’ benefits, (ii) apply utilization management restrictions or high patient cost-sharing obligations or (iii)
restrict  the  level  of  reimbursement  for  our  approved  products  and  any  such  actions  may  affect  our  ability  to  sell  our
approved products on a profitable basis or at all.

Medicare  is  a  U.S.  federal  healthcare  program  that  provides  coverage  for  certain  healthcare  items  and  services  to
individuals aged 65 years or older, as well as individuals of any age with certain disabilities and illnesses. The Medicare
Prescription Drug, Improvement, and Modernization Act of 2003 (“MMA”) imposed new requirements for the distribution
and pricing of prescription drugs for Medicare beneficiaries. Under Part D of the MMA, Medicare beneficiaries may enroll
in prescription drug plans offered by private entities which provide coverage for outpatient prescription drugs. Part D plans
include  both  stand-alone  prescription  drug  benefit  plans  and  prescription  drug  coverage  as  part  of  Medicare  Advantage
plans.  Unlike  Medicare  Part  A  and  B,  Part  D  prescription  drug  plan  sponsors  are  not  required  to  pay  for  all  outpatient
drugs, and each Part D plan can develop its own drug formulary that identifies which drugs it will cover and at what tier or
level. However, Part D plan drug formularies must include at least two drugs within each therapeutic category and class of
Part D drugs, though not necessarily all the drugs in each category or class. Any formulary used by a Part D prescription
drug  plan  must  be  developed  and  reviewed  by  a  pharmacy  and  therapeutics  committee.  Part  D  plan  coverage  and
reimbursement may increase demand for our products for which we receive marketing approval in the United States.

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Moreover,  while  Part  D  provides  prescription  drug  benefits  only  to  Medicare  beneficiaries,  private  payors  often  follow
Medicare coverage policy and payment limitations in setting their own payment rates. Any reduction in reimbursement by
Medicare  may  result  in  a  similar  reduction  in  payments  from  non-governmental  payors.  Medicare  Part  D  may  affect
reimbursement of our products upon approval.

Medicaid is a U.S. healthcare program that provides coverage for certain healthcare items and services to low-income
children, families, pregnant women and people with disabilities. It is jointly funded by the federal and state governments,
and it is administered by individual states within parameters established by the federal government. Therefore, coverage
and  reimbursement  for  drugs  may  vary  by  state  Medicaid  program.  A  manufacturer  must  enter  into  a  Medicaid  Drug
Rebate  Agreement  to  have  its  products  covered  by  Medicaid.  Under  the  Medicaid  program,  and  per  the  Medicaid  Drug
Rebate  Agreement,  manufacturers  agree  to  report  certain  prices  to  the  government  and  pay  rebates  to  state  Medicaid
programs based on Medicaid utilization of the manufacturer’s covered drugs.

In addition to the Medicaid Drug Rebate Program, federal law requires companies to participate in the Public Health
Service’s 340B Drug Pricing Program in order to have the manufacturer’s drugs covered under Medicaid. The 340B Drug
Pricing Program requires participating manufacturers to charge statutorily-defined covered entities no more than the 340B
“ceiling  price”  for  the  manufacturer’s  covered  outpatient  drugs.  The  Patient  Protection  and  Affordable  Care  Act,  as
amended by the Health Care and Education Affordability Reconciliation Act of 2010 (collectively, the “ACA”), extended
eligibility  to  participate  in  the  340B  program  to  certain  additional  types  of  hospitals  (including  critical  access  hospitals,
sole  community  hospitals,  rural  referral  centers  and  freestanding  cancer  hospitals).  For  purposes  of  these  newly  eligible
covered entities, the ACA specifically excluded from the definition of “covered outpatient drugs” certain drugs designated
as  “orphan  drugs”  under  section  526  of  the  FDCA.  We  are  also  required  as  a  condition  of  Medicaid  participation  to
discount our products to authorized users of the Federal Supply Schedule of the General Services Administration, including
the TRICARE retail pharmacy program, under which additional laws and requirements apply.

These  programs  require  submission  of  pricing  data  and  calculation  of  discounts  and  rebates  pursuant  to  complex
statutory formulas, and the guidance governing such calculations is not always clear. Compliance with such requirements
can  require  significant  investment  in  personnel,  systems  and  resources,  but  failure  to  properly  calculate  prices,  or  offer
required discounts or rebates can subject manufacturers to substantial penalties.

In  2010,  the  ACA  was  enacted  to,  among  other  things,  expand  access  and  increase  consumer  insurance  protections
while reducing the cost of health care for consumers. The law substantially changed the way health care is financed by both
governmental and private insurers in the United States. The ACA requires manufacturers to provide discounts on the prices
of  brand  named  drugs  in  the  coverage  gap  under  Medicare  Part  D  and  increased  the  rebates  paid  by  pharmaceutical
companies on drugs covered by Medicaid. The ACA also imposes an annual fee, which increases each year, on sales by
branded pharmaceutical manufacturers. The ACA has been challenged repeatedly in court, and its future is uncertain. If the
ACA is ultimately overturned or repealed, the effect on our business could be material.

There has been particular and increasing legislative and enforcement interest in the United States with respect to drug
pricing practices, particularly with respect to drugs that have been subject to relatively large price increases over relatively
short time periods. At the federal level, there have been several U.S. Congressional inquiries, proposed bills, and proposed
administrative  rules  designed  to,  among  other  things,  bring  more  transparency  to  drug  pricing,  review  the  relationship
between  pricing  and  manufacturer  patient  programs,  and  reform  government  program  reimbursement  methodologies  for
drugs. The outcome and potential effects of these proposals, and other proposals that may be forthcoming is unclear. At the
state  level,  legislatures  have  increasingly  passed  legislation  and  implemented  regulations  designed  to  control
pharmaceutical and biological product pricing, including price or patient reimbursement constraints, discounts, restrictions
on  certain  product  access  and  marketing  cost  disclosure  and  transparency  measures,  and,  in  some  cases,  to  encourage
importation from other countries and bulk purchasing.

In addition, in some non-U.S. jurisdictions, the proposed pricing for a drug must be approved before its cost may be
funded  within  the  respective  national  healthcare  systems.  The  requirements  governing  drug  pricing  vary  widely  from
country  to  country.  For  example,  European  Union  member  states  can  restrict  the  range  of  medicinal  products  for  which
their national health insurance systems provide reimbursement and may control the prices of medicinal products for human
use. A member state may approve a specific price for the medicinal product or it may instead adopt a system of direct or

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indirect controls on the profits the medicinal product generates for the company placing it on the market. There can be no
assurance  that  any  country  that  has  price  controls  or  reimbursement  limitations  for  pharmaceutical  products  will  allow
favorable  reimbursement  and  pricing  arrangements  for  any  of  our  products  on  cost-effectiveness  grounds.  Historically,
products  launched  in  countries  in  the  European  Union  do  not  follow  price  structures  of  the  United  States  and  generally
their prices tend to be significantly lower. In February 2022, ICPT France withdrew its application for reimbursement in
France  of  Ocaliva  for  treatment  of  PBC,  on  account  of  inability  to  reach  mutually  acceptable  pricing  terms  with  CEPS.
ICPT France initiated sales of Ocaliva in France prior to finalization of reimbursement terms pursuant to a temporary use
authorization (“ATU”). As required by French law, ICPT France intends to continue to provide Ocaliva in France for one
year  following  the  closure  of  the  ATU  period,  for  purposes  of  continuity  of  treatment  for  patients  using  Ocaliva.  ICPT
France will continue to work with the French regulators regarding ATU and post-ATU payback.

U.S. Fraud and Abuse Laws

Interactions and arrangements with third-party payors, healthcare providers and professionals and customers, including
patients  and  patient  advocacy  groups,  are  subject  to  broadly  applicable  fraud  and  abuse  and  other  healthcare  laws  and
regulations  that  may  restrict  certain  marketing  and  contracting  practices.  These  laws  include,  federal  and  state  anti-
kickback and false claims statutes as well as other statutes and regulations pertaining to healthcare fraud and abuse. Other
pharmaceutical companies have settled alleged or admitted violations of these fraud and abuse laws with state and federal
authorities in recent years and in some cases these settlements have amounted to hundreds of millions, or even billions, of
dollars in damages, fines, and penalties, as well as the imposition of compliance program obligations through Corporate
Integrity  Agreements  and  other  means.  Lawsuits,  or  enforcement  actions  brought  under  fraud  and  abuse  laws,  can  be
extremely  costly  to  defend,  even  if  a  company  has  strong  defenses  and  ultimately  succeeds  in  getting  the  allegations  or
enforcement action dismissed.

The federal Anti-Kickback Statute (42 U.S.C. §1320a-7b(b)) prohibits, among other things, knowingly and willfully
soliciting, receiving, offering or providing remuneration, directly or indirectly, to induce either the referral of an individual,
or the furnishing, recommending, or arranging for any good or service, for which payment may be made under federal and
state  healthcare  programs  such  as  Medicare,  Medicaid  or  other  federally  financed  healthcare  programs.  Remuneration  is
not  defined  in  the  federal  Anti-Kickback  Statute  and  has  been  broadly  interpreted  by  regulators  to  include  for  example,
cash payments, gifts, discounts, coupons, and the furnishing of free or discounted services or supplies, and other items or
services  of  value  to  the  recipient.  This  statute  has  been  broadly  interpreted  to  apply  to  manufacturer  arrangements  with
prescribers,  purchasers,  formulary  managers  and  patients,  among  others.  Although  there  are  a  number  of  statutory
exceptions and regulatory safe harbors protecting certain common activities from prosecution or other regulatory sanctions,
the  exceptions  and  safe  harbors  are  drawn  narrowly,  and  practices  that  involve  remuneration  intended  to  induce
prescribing, purchases or recommendations may be subject to scrutiny if they do not qualify for such exceptions or safe
harbors.

The  federal  False  Claims  Act  imposes  civil  penalties,  including  treble  damages  and  significant  per-claim  penalties,
which  may  be  pursued  through  civil  whistleblower  or  qui  tam  actions,  against  individuals  or  entities  for  knowingly
presenting, or causing to be presented, to the federal government, claims for payment that are false or fraudulent or making
a false statement to avoid, decrease or conceal an obligation to pay money to the federal government. The government and
qui tam relators have brought False Claims Act actions against pharmaceutical companies on the theory that their practices
have  caused  false  claims  to  be  presented  to  the  government.  There  is  also  a  separate  false  claims  provision  imposing
criminal penalties.

Other  federal  healthcare  fraud-related  laws  also  impose  criminal  liability  for  violations.  The  Criminal  Healthcare
Fraud statute (18 U.S.C. §1347) prohibits knowingly and willfully executing a scheme to defraud any healthcare benefit
program,  including  private  third-party  payers.  Federal  criminal  law  also  prohibits  knowingly  and  willfully  falsifying,
concealing or covering up a material fact or making any materially false, fictitious or fraudulent statement in connection
with the delivery of or payment for healthcare benefits, items or services.

A number of states also have statutes or regulations similar to the federal Anti-Kickback Statute and False Claims Act
that  apply  to  items  and  services  reimbursed  under  Medicaid  and  other  state  programs.  Some  state  anti-kickback  statutes
apply not just to government payors, but to all payors, including commercial payors and patients.

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Other Laws

The Health Insurance Portability and Accountability Act of 1996, as amended by the Health Information Technology
for Economic and Clinical Health Act (collectively, “HIPAA”), imposes obligations, on “covered entities,” including health
plans  and  healthcare  providers,  and  their  business  associates  with  respect  to  safeguarding  the  privacy,  security  and
transmission  of  individually  identifiable  health  information.  Although  drug  manufacturers  are  not  directly  subject  to
HIPAA,  we  could  be  subject  to  criminal  or  civil  penalties  if  we  knowingly  obtain  individually  identifiable  health
information from a HIPAA-covered entity in a manner that is not authorized or permitted by HIPAA. We are also subject to
state,  federal  and  international  privacy  and  security  laws  governing  the  processing  and  security  of  personal  identifiable
information.

The federal Physician Payments Sunshine Act requirements under the ACA, and its implementing regulations, require
manufacturers  of  drugs,  devices,  biologics  and  medical  supplies  to  report  to  the  U.S.  Department  of  Health  and  Human
Services information related to certain direct and indirect payments and other transfers of value made to covered recipients,
such  as  physicians  and  teaching  hospitals,  as  well  as  ownership  and  investment  interests  held  by  physicians  and  their
immediate family members. Payments made to physicians and research institutions for clinical trials are included within
the ambit of this law. We are also subject to similar laws in several states and various European Union countries where we
have operations. Some of these state and EU laws are broader in scope than federal laws.

In addition, several states now require prescription drug companies to report expenses relating to the marketing and
promotion of drug products. Several states prohibit providing certain payments or items of value to healthcare providers or
other  enumerated  individuals  or  entities,  as  well  as  various  other  marketing-related  activities.  Certain  states  require  the
posting  of  information  relating  to  clinical  studies  and  their  outcomes.  In  addition,  several  states  require  pharmaceutical
companies  to  implement  compliance  programs  and  marketing  codes,  and  additional  states  are  considering  similar
proposals. Also, some states and localities require sales representatives to be registered or licensed. Some of the state laws
are  broader  in  scope  than  federal  laws.  Compliance  with  these  laws  is  challenging  and  requires  significant  time  and
resources,  and  any  failure  to  comply  with  such  laws  could  result  in  significant  civil  penalties  and  other  adverse
consequences.

Human Capital Resources

As  of  December  31,  2021,  we  had  437  employees,  of  which  319  were  based  in  the  United  States,  including  at  our
facilities in New York and San Diego, and 118 were based outside the United States, including at our offices in London. A
significant percentage of our employees have obtained advanced degrees in their professions. None of our employees are
represented by a labor union and we consider our employee relations to be good.

We consider the intellectual capital of our employees to be an essential driver of our business and key to our future
prospects.  Given  our  leadership  in  the  treatment  of  progressive  non-viral  liver  disease  coupled  with  our  disciplined
management  of  our  financial  resources,  we  continue  to  be  able  to  fill  the  vacated  positions  and,  if  needed,  grow  our
headcount in support of our commercial organization and our pipeline of research and development programs and product
candidates.  In  addition,  we  continually  evaluate  our  headcount  with  respect  to  our  business  needs  and  opportunities  and
seek to balance in house expertise and capacity with outsourced expertise and capacity.

We  monitor  our  compensation  programs  closely  and  provide  what  we  consider  to  be  a  competitive  mix  of

compensation and insurance benefits for our employees, as well as participation in our equity programs.

We offer employees a number of additional resources and tools to help in their personal and professional development,
including career development planning, professional assessment and feedback tools, and wellness programs through which
employees may access information regarding scheduled healthy lifestyle activities, articles and other beneficial resources.

We are committed to hiring, developing and supporting a diverse and inclusive workplace, and continue to focus on
extending our equality, diversity and inclusion initiatives across our workforce. Our virtual Diversity, Equity, and Inclusion
(DEI) Hub recognizes the power of a diverse, equitable and inclusive work force, and how it enriches the professional lives

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of team members, drives innovation, and connects the Company to the patients and communities it serves. Employees have
access to internally produced resources, articles, and toolkits, as well as a virtual DEI calendar.

In  response  to  the  COVID-19  pandemic  and  related  risk  mitigation  efforts,  we  assembled  a  COVID-19  task  force,
which  consists  of  leaders  from  various  departments  within  our  organization,  and  is  responsible  for  monitoring
developments  related  to  the  COVID-19  pandemic  and  implementing  safety  policies  and  procedures.  Our  office-based
employees  have  been  largely  working  remotely  and  we  have  leveraged  digital  communication  technologies  where
appropriate to facilitate interactions with patients, healthcare professionals and our other stakeholders.

Corporate and Available Information

We were incorporated in Delaware in September 2002. Our principal executive offices are located at 10 Hudson Yards,
37th  Floor,  New  York,  NY  10001  and  our  telephone  number  is  (646)  747-1000.  We  have  several  additional  offices,
including  those  in  San  Diego,  California  and  London,  United  Kingdom.  We  are  in  the  process  of  moving  our  principal
executive  offices  to  305  Madison  Avenue,  Morristown,  NJ  07960,  in  connection  with  the  expiration  of  our  lease  at  10
Hudson Yards.

Our  corporate  website  address  is  www.interceptpharma.com.  We  make  available  on  our  website,  free  of  charge,  our
Annual Reports on Form 10-K, Quarterly Reports on Form 10-Q, Current Reports on Form 8-K and any amendments to
those reports filed or furnished pursuant to Section 13(a) or 15(d) of the Securities Exchange Act of 1934, as amended (the
“Exchange  Act”),  as  soon  as  reasonably  practicable  after  we  electronically  file  such  material  with,  or  furnish  it  to,  the
Securities and Exchange Commission (“SEC”). Our SEC reports can be accessed through the Investors & Media section of
our  internet  website.  The  references  to  www.interceptpharma.com  herein  are  inactive  textual  references  only,  and  the
information found on our internet website is not incorporated by reference into this Annual Report on Form 10-K or any
other  report  we  file  with  or  furnish  to  the  SEC.  The  SEC  maintains  an  internet  website  that  contains  reports,  proxy  and
information statements and other information about issuers, like us, that file electronically with the SEC. The address of
that site is http://www.sec.gov.

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Item 1A.  Risk Factors

Investing in our securities involves a high degree of risk. The following risk factors and other information included in
this Annual Report on Form 10-K should be carefully considered before deciding whether to invest in our securities. The
risks  and  uncertainties  described  below  and  in  our  other  filings  are  not  the  only  ones  we  face.  Additional  risks  and
uncertainties not presently known to us or that we presently deem less significant may also impair our business operations.
If  any  of  the  following  risks,  or  such  unknown  risks,  occur,  our  business,  financial  condition,  results  of  operations  and
future growth prospects could be materially and adversely affected. In that case, the market price of our securities could
decline, and you may lose all or part of your investment.

Risks Related to Our Financial Position and Need for Additional Capital

We  are  currently  dependent  on  the  successful  commercialization  of  Ocaliva  for  PBC.  To  the  extent  Ocaliva  is  not
commercially  successful,  our  business,  financial  condition  and  results  of  operations  may  be  materially  and  adversely
affected and the price of our common stock may decline.

Ocaliva is our only drug that has been approved for sale and it has only been approved for the treatment of PBC in
combination with UDCA in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate
UDCA.

Our ability to generate profits from operations and become profitable currently depends on the commercial success of
Ocaliva for PBC. However, the successful commercialization of Ocaliva for PBC is subject to many risks. We have not
launched or commercialized a drug before Ocaliva, and there is no guarantee that we will be able to do so successfully.
There  are  numerous  examples  of  unsuccessful  product  launches  and  commercial  efforts,  as  well  as  failures  to  meet
expectations of market potential, including by pharmaceutical companies with greater experience and resources than us.

The commercial success of Ocaliva for PBC depends on the extent to which patients, physicians and payers accept and
adopt Ocaliva as a treatment for PBC, and we do not know whether our or others’ estimates in this regard will be accurate.
As such, there is significant uncertainty in the degree of market acceptance that Ocaliva will have for PBC. For example, if
the  patient  population  suffering  from  PBC  is  smaller  than  we  estimate,  or  even  if  the  patient  population  matches  our
estimates but Ocaliva is not widely accepted as a treatment for PBC, the commercial potential of Ocaliva for PBC will be
limited. Physicians may not prescribe Ocaliva and patients may be unwilling to use Ocaliva if coverage is not provided or
reimbursement is inadequate to cover a significant portion of the cost. Additionally, the use of Ocaliva in a non-trial setting
may  result  in  the  occurrence  of  unexpected  or  a  greater  incidence  of  side  effects,  adverse  reactions  or  misuse  that  may
negatively  affect  the  commercial  prospects  of  Ocaliva  for  PBC.  Furthermore,  any  negative  development  in  any  other
development program for OCA or our failure to satisfy the post-marketing regulatory commitments and requirements to
which we are or may become subject including the submission of data from our Phase 4 COBALT trial or any other study
to assess the clinical benefit of Ocaliva in PBC may materially and adversely impact the commercial results and potential
of Ocaliva for PBC. In May 2021, we updated the Ocaliva prescribing information in the United States and Ocaliva is now
contraindicated  for  patients  with  PBC  and  decompensated  cirrhosis,  a  prior  decompensation  event,  or  compensated
cirrhosis with evidence of portal hypertension, in addition to the existing contraindication for complete biliary obstruction.
Corresponding  limitations  on  the  use  of  Ocaliva  in  our  potential  patient  population,  or  similar  safety  concerns,  could
reduce our sales. See “—Risks Related to the Development and the Regulatory Review and Approval of Our Products and
Product Candidates” and “—Risks Related to the Commercialization of Our Products” below.

As a result, it is uncertain whether Ocaliva net sales for PBC will sustain our operations and it may take a significant
amount of time before Ocaliva net sales for PBC sustain our operations. Furthermore, Ocaliva may not receive regulatory
approval for PBC in jurisdictions beyond those in which it is currently approved, which may also limit our prospects. If the
commercialization of Ocaliva for PBC is unsuccessful or perceived to be unsuccessful, the long-term prospects of Ocaliva
for PBC, as well as the long-term prospects of our company, may be materially and adversely affected.

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We  have  never  been  profitable.  We  expect  to  incur  losses  for  the  foreseeable  future,  and  we  may  never  achieve  or
sustain profitability.

We have never been profitable and do not expect to be profitable in the foreseeable future. We incurred net losses of
$91.4 million, $274.9 million and $344.7 million for the years ended December 31, 2021, 2020 and 2019, respectively. To
date, we have financed our operations primarily through public offerings and private placements of our securities, sales of
product  and  payments  received  under  licensing  and  collaboration  agreements.  At  December  31,  2021,  we  had  $429.4
million in cash, cash equivalents, restricted cash and investment debt securities.

We have devoted substantially all of our resources to the development of our product candidates, including the conduct
of our clinical trials, the launch and commercialization of Ocaliva for PBC, preparation for a potential launch of OCA for
liver fibrosis due to NASH and general and administrative operations, including the protection of our intellectual property.

We  expect  to  continue  to  incur  losses  for  the  foreseeable  future,  and  we  expect  these  losses  to  be  significant  as  we,
among other things, develop and seek regulatory approval for our product candidates, including OCA for liver fibrosis due
to  NASH,  maintain  our  regulatory  approvals  and  commercialize  our  approved  products.  We  believe  our  prospects  and
ability to significantly grow revenues will be dependent on our ability to successfully develop and commercialize OCA for
indications other than PBC, such as NASH, and to identify strategic business development opportunities to leverage our
capabilities  in  rare  diseases.  As  a  result,  we  expect  a  significant  amount  of  resources  to  continue  to  be  devoted  to  our
development programs for OCA and to developing our pipeline.

As part of our product development activities, we currently expect to continue our Phase 3 clinical program of OCA for
liver fibrosis due to NASH, including our Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH through
clinical outcomes for verification and description of clinical benefit and our Phase 3 REVERSE trial for NASH patients
with compensated cirrhosis. Our expenses could increase if we are required by the FDA or the EMA to perform studies or
trials in addition to those currently expected, if our current trials are modified for any reason, or if there are any issues or
delays  in  completing  our  clinical  trials  or  the  development  of  any  of  our  product  candidates,  due  to  COVID  19  or
otherwise.  For  example,  in  June  2020  we  received  a  CRL  from  the  FDA  with  respect  to  our  NDA  for  OCA  for  liver
fibrosis due to NASH. The CRL indicated that, based on the data the FDA had reviewed, the FDA has determined that the
predicted  benefit  of  OCA  based  on  a  surrogate  histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing
REGENERATE trial in support of potential accelerated approval and that the long-term outcomes phase of the trial should
continue.  Although  we  are  in  discussions  with  the  FDA  with  respect  to  the  potential  resubmission  of  our  NDA  seeking
accelerated  approval  of  OCA  for  the  treatment  of  liver  fibrosis  due  to  NASH,  there  is  no  assurance  that  we  will  be
successful or that OCA will be approved for liver fibrosis due to NASH on an accelerated basis, or at all. Accordingly, our
previously  anticipated  U.S.  commercial  launch  of  OCA  for  liver  fibrosis  due  to  NASH  has  been  postponed,  we  do  not
expect to generate revenues for this indication until it has been approved, and we may incur significantly greater costs than
previously anticipated in connection with the development of OCA for liver fibrosis due to NASH.

We intend to continue to develop OCA and our other existing product candidates, alone or in combination, for non-viral
liver diseases. If OCA or any of our other product candidates fails in clinical trials or does not gain or maintain regulatory
approval, or if OCA or any of our other product candidates does not achieve market acceptance, we may never become
profitable.  Our  net  losses  and  negative  cash  flows  have  had,  and  will  continue  to  have,  an  adverse  effect  on  our
stockholders’ equity and working capital. Because of the numerous risks and uncertainties associated with pharmaceutical
product development and commercialization, we are unable to predict with certainty the timing or amount of our expenses,
whether such expenses may increase, or when, or if, we will be able to achieve profitability. The amount of our future net
losses will depend, in part, on our future expenses, whether and by how much such expenses increase and our ability to
generate revenues.

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We  will  require  substantial  additional  funding,  which  may  not  be  available  to  us  on  acceptable  terms,  if  at  all.  If
adequate funds are not available to us, we may be required to delay, limit, reduce or cease our operations.

We are currently developing OCA for additional indications, including NASH, and other product candidates through
various  stages  of  clinical  and  preclinical  development.  Developing  pharmaceutical  products,  including  conducting
preclinical studies and clinical trials, is expensive. If, for example, the FDA, EMA or other regulatory authorities require
that we perform additional studies beyond those that we currently expect, our expenses could increase materially beyond
what we currently anticipate, and the timing of any potential product approval may be delayed.

In  addition,  we  have  incurred  and  anticipate  that  we  will  continue  to  incur  significant  research  and  development,
product sales, marketing, manufacturing and distribution expenses relating to the commercialization of Ocaliva for PBC.
As part of our longer-term strategy, we anticipate that we will incur significant expenses in connection with our research
and  development  efforts,  the  commercialization  of  our  other  products  such  as  OCA  for  liver  fibrosis  due  to  NASH,  if
approved, and the maintenance of our general and administrative infrastructure in the United States and abroad. We may
also  engage  in  business  development  activities  that  involve  potential  in-  or  out-licensing  of  products  or  technologies  or
acquisitions of other products, technologies or businesses.

As  of  December  31,  2021,  we  had  $429.4  million  in  cash,  cash  equivalents,  restricted  cash  and  investment  debt
securities. We currently expect to continue to incur significant operating expenses in the fiscal year ending December 31,
2022. These expenses are planned to support, among other initiatives, the continued commercialization of Ocaliva for PBC
in the United States and our other markets, our continued clinical development of OCA for PBC and NASH and our other
earlier stage research and development programs. Although we believe that our existing capital resources, together with our
net sales of Ocaliva for PBC, will be sufficient to fund our anticipated operating requirements for the next twelve months,
we may need to raise additional capital to fund our operating requirements beyond that period. Furthermore, in light of our
receipt in June 2020 of a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to NASH and the
numerous risks and uncertainties associated with pharmaceutical product development and commercialization, any delays
in,  or  unanticipated  costs  associated  with,  our  development,  regulatory  or  commercialization  efforts  could  significantly
increase the amount of capital required by us to fund our operating requirements. Accordingly, we may seek to access the
public  or  private  capital  markets  whenever  conditions  are  favorable,  even  if  we  do  not  have  an  immediate  need  for
additional capital at that time.

Our forecasts regarding the period of time that our existing capital resources will be sufficient to meet our operating
requirements  and  the  timing  of  our  future  funding  requirements,  both  near  and  long-term,  will  depend  on  a  variety  of
factors, many of which are outside of our control. Such factors include, but are not limited to, those factors listed above
under “Cautionary Note Regarding Forward-Looking Statements”.

We have no committed external sources of funding and additional funds may not be available when we need them on
terms that are acceptable to us, or at all. If adequate funds are not available to us, we may not be able to make scheduled
debt payments on a timely basis, or at all, and may be required to delay, limit, reduce or cease our operations.

Raising  additional  capital  may  cause  dilution  to  our  stockholders,  restrict  our  operations  or  require  us  to  relinquish
rights to our technologies or product candidates.

Unless  and  until  we  generate  sufficient  cash  flow  from  sales  of  our  products,  including  Ocaliva  for  PBC  and,  if
approved, OCA for liver fibrosis due to NASH, we expect to finance our future cash needs through public or private equity
or  debt  financings,  government  or  other  third-party  funding,  marketing  and  distribution  arrangements  or  other
collaborations, strategic alliances and licensing arrangements, or a combination of these sources. Additional funding may
not be available to us on acceptable terms, if at all.

The terms of any future financing may adversely affect the interests of our existing securityholders. For example, to
the  extent  that  we  raise  additional  capital  through  the  sale  of  equity  or  convertible  debt  securities,  our  stockholders’
ownership  interest  will  be  diluted,  and  the  terms  of  these  securities  may  include  liquidation  or  other  preferences  that
adversely affect the rights of our common stockholders. Debt financing, if available, may involve agreements that include

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covenants  limiting  or  restricting  our  ability  to  take  specific  actions,  such  as  incurring  additional  debt,  making  capital
expenditures or declaring dividends, in addition to covenants under our existing debt financings. We also could be required
to seek funds through arrangements with licensing or collaborative partners or otherwise that may require us to relinquish
rights to some of our technologies or product candidates or otherwise agree to terms unfavorable to us. If we are unable to
raise  additional  funds  through  equity  or  debt  financings  when  needed,  we  may  be  required  to  delay,  limit,  reduce  or
terminate  our  product  development  or  future  commercialization  efforts  or  grant  rights  to  develop  and  market  product
candidates that we would otherwise prefer to develop and market ourselves.

Risks Related to the Development and the Regulatory Review and
Approval of Our Products and Product Candidates

We  cannot  be  certain  whether  Ocaliva  will  receive  full  approval  for  PBC  in  jurisdictions  where  it  has  previously
received accelerated or conditional approval, or that Ocaliva will be approved for PBC in any jurisdictions beyond those
in which it is currently approved. Furthermore, OCA may not be approved on an accelerated basis, or at all, for NASH
or  any  other  indication  beyond  PBC  and  we  may  not  receive  regulatory  approval  for  any  other  product  candidate.
Without regulatory approval, we will not be able to market and commercialize our product candidates.

The  development,  testing,  manufacture,  packaging,  labeling,  storage,  approval,  promotion,  advertising,  distribution,
marketing  and  export  and  import,  among  other  things,  of  our  products  and  product  candidates  are  subject  to  extensive
regulation by the FDA in the United States, the EMA in Europe and various regulatory authorities in other countries, with
regulations differing from country to country. We are not permitted to market our product candidates in the United States or
Europe  until  we  receive  approval  of  a  NDA,  from  the  FDA,  or  a  MAA,  from  the  European  Commission,  respectively.
Currently, our ability to generate product sales depends on the successful marketing of Ocaliva for PBC in the jurisdictions
in  which  it  has  received  regulatory  approval.  In  the  future,  our  ability  to  generate  product  sales  in  addition  to  those  of
Ocaliva  for  PBC  will  depend  on  whether  we  are  successful  in  obtaining  regulatory  approval  of  our  other  product
candidates, including OCA for liver fibrosis due to NASH.

Ocaliva is our only drug that has been approved for sale and it has only been approved for the treatment of PBC in
combination with UDCA in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate
UDCA. In the United States, Ocaliva was approved for PBC under the accelerated approval pathway. Accelerated approval
was  granted  for  Ocaliva  for  PBC  based  on  a  reduction  in  ALP;  however,  an  improvement  in  survival  or  disease-related
symptoms has not yet been established. Continued approval of Ocaliva for PBC in the United States is contingent upon the
verification  and  description  of  clinical  benefit  in  confirmatory  trials  and  our  satisfaction  of  our  other  post-marketing
regulatory requirements. Any failure by us to confirm the clinical benefit of Ocaliva for PBC due to COVID-19 or other
factors may jeopardize the continued approval of Ocaliva for PBC.

We  commenced  our  commercial  launch  of  Ocaliva  for  PBC  in  certain  European  countries  in  2017  following  the
European  Commission’s  grant  of  conditional  approval  in  December  2016.  Our  marketing  authorization  in  the  European
Union was granted on the condition of the successful completion of the COBALT trial and our “401 trial” evaluating the
safety and efficacy of Ocaliva in patients with moderate to severe hepatic impairment. We have closed our 401 trial and are
in the process of closing our COBALT trial. We are in discussions with the FDA and EMA with respect to the future of our
post-marketing commitments.

Since January 2017, Ocaliva has also received regulatory approval in several of our target markets outside the United
States  and  Europe,  including  (but  not  limited  to)  Canada,  Israel,  and  Australia,  and  we  continue  to  pursue  marketing
approval of Ocaliva for PBC in our other international target markets. If obtained, continued approval of Ocaliva for PBC
in such jurisdictions may be contingent upon the verification and description of clinical benefit in confirmatory trials. Any
delay or failure in satisfying the post-marketing regulatory commitments and requirements to which we are or may become
subject  may  jeopardize  the  continued  approval  of  Ocaliva  for  PBC  in  the  United  States,  European  Union  and  other
jurisdictions. In some markets where regulatory approval has been obtained for Ocaliva, discussions with national public
health system authorities regarding reimbursement are ongoing. In February 2022, ICPT France withdrew its application
for reimbursement in France of Ocaliva for treatment of PBC, on account of inability to reach mutually acceptable pricing
terms with CEPS. ICPT France initiated sales of Ocaliva in France prior to finalization of reimbursement terms pursuant to
an ATU. As required by French law, ICPT France intends to continue to provide Ocaliva in France for one year

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following the closure of the ATU period, for purposes of continuity of treatment for patients using Ocaliva. ICPT France
will continue to work with the French regulators regarding ATU and post-ATU payback.

Changes to our Ocaliva label with respect to patients with PBC with decompensated cirrhosis (e.g., Child-Pugh Class
B  or  C),  a  prior  decompensation  event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension  influenced
modifications  to  our  COBALT  study  design  and  as  a  result  of  the  changes  to  the  U.S.  prescribing  information  we  also
removed from the trial subjects in the United States who are now excluded from the scope of the label. We also agreed with
the  FDA  and  the  EMA  to  terminate  our  401  trial,  in  light  of  the  exclusion  of  patients  with  PBC  with  decompensated
cirrhosis from the Ocaliva label in the U.S. In addition, while we remain blinded to safety and efficacy data in these trials,
the Data Monitoring Committee (“DMC”) reviewed the unblinded results of a pre-specified interim efficacy analysis of the
COBALT trial and separately reviewed unblinded safety and pharmacokinetic data from both the COBALT and 401 trials.
Following these reviews, the DMC stated that it was not feasible to continue the COBALT trial as designed and noted the
challenges  in  enrolling  and  maintaining  placebo-controlled  post-marketing  studies  in  this  rare  disease  setting.  No  acute
safety  concerns  were  noted  by  the  DMC.  Given  the  feasibility  concerns  noted  by  the  DMC  as  well  as  the  potential
confounding  impact  of  subjects  discontinuing  treatment  and/or  transitioning  from  investigational  product  to  commercial
drug during clinical trials, we discussed with the FDA and the EMA proposed modifications to the COBALT trial, and we
notified the FDA and the EMA of the DMC’s recommendation. Based on discussions with both the FDA and EMA, which
are ongoing, we closed our 401 trial and are in the process of closing out the COBALT trial. We will continue to generate
placebo controlled data from the COBALT trial as well as data from studies utilizing real world evidence in support of a
broader evidence data package, which we anticipate submitting to the FDA and the EMA in the second half of 2022. If this
data package does not support fulfillment of our post-marketing obligations, we may not be able to maintain our previously
granted marketing approvals of Ocaliva for PBC.

Ocaliva is not approved for any indication other than PBC. We currently have no other products approved for sale and
we  cannot  guarantee  that  we  will  ever  have  additional  marketable  products  or  that  OCA  will  be  approved  for  use  in
additional indications such as NASH. NDAs and MAAs must include extensive preclinical and clinical data and supporting
information  to  establish  the  product  candidate’s  safety  and  effectiveness  for  each  desired  indication.  NDAs  and  MAAs
must also include significant information regarding the chemistry, manufacturing and controls for the product. Obtaining
approval of a NDA or a MAA is a lengthy, expensive and uncertain process, and we may not be successful in obtaining
approval. The FDA and the EMA review processes can take years to complete and approval is not guaranteed. Even after
the submission of a NDA, the FDA may decide not to accept the submission for filing and review or may determine that
the submission does not support approval. For example, in June 2020 we received a CRL from the FDA with respect to our
NDA for OCA for liver fibrosis due to NASH. The CRL indicated that, based on the data the FDA had reviewed, the FDA
had  determined  that  the  predicted  benefit  of  OCA  based  on  a  surrogate  histopathologic  endpoint  remains  uncertain  and
does  not  sufficiently  outweigh  the  potential  risks  to  support  accelerated  approval  for  the  treatment  of  patients  with  liver
fibrosis  due  to  NASH.  The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data
from the ongoing REGENERATE study in support of potential accelerated approval and that the long-term outcomes phase
of the study should continue. In December 2021, the Company withdrew its MAA as the established application timeline
could not be extended any further to allow for submission of additional safety and efficacy data being generated from the
REGENERATE study and the CHMP was not able to determine a positive benefit-risk based on previously submitted data.
Once the additional data from REGENERATE becomes available, the Company will assess the possibility of submitting a
new application to the EMA.

The United Kingdom left the European Union on January 31, 2020, in what is often referred to as “Brexit,” and the
end of the transition period was December 31, 2020. Thus, Brexit came into effect on January 1, 2021, at which time the
existing  centrally  approved  marketing  authorization  for  Ocaliva  was  automatically  converted  into  a  UK  marketing
authorization  by  the  UK  medicines  regulator,  MHRA  (the  so-called  “grandfathering”  process).  Over  time,  Brexit  may
result  in  material  changes  to  the  regulations  applicable  to  us.  Continuing  threats  from  COVID-19,  including  additional
waves of infections, could also affect the operations of the FDA, EMA and other health authorities, which could delay our
clinical development efforts and the review and approval of our product candidates, including OCA for liver fibrosis due to
NASH.

As is the case with the approval of Ocaliva for PBC, any future approvals or potential future approvals may also be

conditional upon the completion of one or more clinical trials. In addition, delays in approvals or rejections of marketing

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applications  in  the  United  States,  Europe  or  other  countries  may  be  based  upon  many  factors,  including,  for  example,
regulatory  requests  for  additional  analyses,  reports,  data,  preclinical  studies  and  clinical  trials,  regulatory  endpoint
requirements,  regulatory  questions  regarding  safety  or  risk-benefit  profile,  different  interpretations  of  data  and  results,
changes in regulatory policy during the period of product development and the emergence of new information regarding
our product candidates or approved products. Initial and continued regulatory approval is also dependent on successfully
passing regulatory inspection requirements applicable to us, our clinical sites and our key vendors, including requirements
that we and such parties comply with applicable good clinical, pharmacovigilance, laboratory and manufacturing practices
regulations.  Critical  findings  could  jeopardize  or  delay  the  approval  of  our  NDAs  or  MAAs  or  impair  our  ability  to
maintain our marketing approvals.

Prior to receiving regulatory approval, we must finalize the product label for each of our product candidates in each
jurisdiction  in  which  we  seek  regulatory  approval.  Even  if  our  product  is  approved,  the  FDA,  EMA  or  other  applicable
regulatory authorities may limit the indications or uses for which our product may be marketed, require extensive warnings
on the product labeling or require expensive and time-consuming clinical trials, risk mitigation programs such as a REMS,
monitoring or reporting as a condition of approval. Also, regulatory approval for our approved products may be withdrawn.
In addition, obtaining regulatory approval for the marketing of our product in one country does not ensure that we will be
able to obtain regulatory approval for such product in any other country.

In  order  to  obtain  and/or  maintain  regulatory  approval  for  OCA  for  indications  other  than  PBC,  we  will  need  to
complete additional clinical trials and studies. For example, in connection with our Phase 3 clinical program of OCA for
liver fibrosis due to NASH, we are currently conducting our Phase 3 REGENERATE trial in patients with liver fibrosis due
to NASH through clinical outcomes for verification and description of clinical benefit and our Phase 3 REVERSE trial for
NASH  patients  with  compensated  cirrhosis.  Our  ability  to  obtain  and  maintain  the  regulatory  approvals  necessary  to
commercialize OCA for indications other than PBC, including NASH, will depend on our ability to successfully design,
conduct and complete these trials, the efficacy, safety and risk-benefit profile of OCA demonstrated by such trials and our
ability to prepare and submit complex regulatory filings in accordance with applicable regulatory requirements.

There can be no assurance that OCA will receive marketing approval on an accelerated or conditional basis, or at all,
for  PBC  in  jurisdictions  where  it  has  not  yet  been  approved  or  for  NASH  in  any  jurisdiction,  or  that  any  of  our  other
product candidates will receive marketing approval for any indication in any jurisdiction. We cannot predict whether our
clinical  trials  and  studies  for  our  product  candidates,  including  OCA  for  PBC,  NASH  or  any  other  indication,  will  be
successful,  whether  regulatory  authorities  will  agree  with  our  conclusions  relating  to  the  clinical  trials  and  studies  we
conduct, or whether such regulatory authorities will require us to conduct additional clinical trials or studies. For example,
while OCA received breakthrough therapy designation from the FDA in January 2015 for the treatment of NASH patients
with liver fibrosis and we filed a NDA in the United States and a MAA in Europe based on the results from the 18-month
analysis of our Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH, we do not know if one pivotal
clinical trial will be sufficient for marketing approval or if regulatory authorities in the United States, the European Union,
or any of our other target markets will approve OCA for liver fibrosis due to NASH on an accelerated or conditional basis,
or at all. Our Phase 3 REGENERATE trial remains blinded after the interim analysis and is expected to continue to follow
patients until the occurrence of a pre-specified number of adverse clinical outcomes, including progression to cirrhosis, for
verification and description of clinical benefit.

If  we  are  unable  to  obtain  regulatory  approval  for  OCA  for  PBC  in  the  jurisdictions  in  which  it  is  not  currently
approved  or  obtain  regulatory  approval  in  the  United  States,  European  Union  and  other  jurisdictions  for  OCA  for  other
indications,  such  as  NASH,  or  for  our  other  product  candidates,  we  may  not  be  able  to  generate  sufficient  revenue  to
become profitable or to continue our operations.

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We are developing product candidates for the treatment of rare diseases or diseases for which there are no or limited
therapies,  such  as  PBC  and  NASH,  and  for  some  of  which  there  is  little  clinical  experience,  and  our  development
approach involves new endpoints and methodologies. As a result, there is a heightened risk that we will not be able to
gain agreement with regulatory authorities regarding an acceptable development plan, that the outcome of our clinical
trials will not be favorable or that, even if favorable, regulatory authorities may not find the results of our clinical trials
to be sufficient for marketing approval.

We are focused on developing therapeutics for the treatment of rare diseases and diseases for which there are no or
limited treatments. As a result, the design and conduct of our clinical trials for these indications is subject to heightened
risk.

In the United States, the FDA generally requires two adequate and well-controlled pivotal clinical trials to approve a
NDA. Furthermore, for full approval of a NDA, the FDA requires a demonstration of efficacy based on a clinical benefit
endpoint.  The  FDA  may  grant  accelerated  approval  based  on  a  surrogate  endpoint  reasonably  likely  to  predict  clinical
benefit. Even though our pivotal clinical trials for a specific indication, such as our Phase 3 REGENERATE trial of OCA in
patients with liver fibrosis due to NASH and our Phase 3 REVERSE trial for NASH patients with compensated cirrhosis,
may achieve their primary endpoints and are reasonably believed by us to be likely to predict clinical benefit, the FDA may
not accept the results of such trials or approve our product candidate on an accelerated basis, or at all. It is also possible
that the FDA may refuse to accept for filing and review any regulatory application we submit for regulatory approval in the
United States. Even if our regulatory application is accepted for review, there may be delays in the FDA’s review process
and the FDA may determine that such regulatory application does not contain adequate clinical or other data or support the
approval  of  the  product  candidate.  In  such  a  case,  the  FDA  may  issue  a  CRL  that  may  require  that  we  conduct  and/or
complete additional clinical trials and preclinical studies or provide additional information or data before it will reconsider
our application for approval. For example, in June 2020 we received a CRL from the FDA regarding our NDA for OCA for
liver fibrosis due to NASH. The CRL indicated that, based on the data the FDA had reviewed, the FDA had determined
that the predicted benefit of OCA based on a surrogate histopathologic endpoint remains uncertain and does not sufficiently
outweigh the potential risks to support accelerated approval for the treatment of patients with liver fibrosis due to NASH.
The  FDA  recommended  that  we  submit  additional  post-interim  analysis  efficacy  and  safety  data  from  the  ongoing
REGENERATE  study  in  support  of  potential  accelerated  approval  and  that  the  long-term  outcomes  phase  of  the  study
should continue. The requirements imposed by the FDA may be substantial, expensive and time-consuming, and there is no
guarantee  that  we  will  continue  to  pursue  any  such  application  or  that  the  FDA  will  ultimately  decide  that  any  such
application supports the approval of the product candidate on an accelerated basis, or at all. The FDA may also refer any
regulatory application to an advisory committee for review and recommendation as to whether, and under what conditions,
the  application  should  be  approved.  While  the  FDA  is  not  bound  by  the  recommendation  of  an  advisory  committee,  it
considers such recommendations carefully when making decisions.

Even if we receive accelerated approval for any of our product candidates, we may be required to conduct or complete
a  post-approval  clinical  outcomes  trial  to  confirm  the  clinical  benefit  of  such  product  candidates  by  demonstrating  the
correlation  of  the  surrogate  endpoint  therapeutic  response  in  patients  with  a  significant  reduction  in  adverse  clinical
outcomes over time. For example, interim analysis results at 18 months in our Phase 3 REGENERATE trial were based on
surrogate endpoints and the impact on clinical outcomes has not been confirmed. The REGENERATE trial is ongoing for
verification and description of clinical benefit of OCA for liver fibrosis due to NASH. There can be no assurance that the
clinical  outcomes  portion  of  our  REGENERATE  trial  will  confirm  that  the  surrogate  endpoint  used  as  the  basis  of  the
regulatory  submissions  we  have  made  or  expect  to  make  seeking  approval  of  OCA  for  liver  fibrosis  due  to  NASH  will
eventually show an adequate correlation with clinical outcomes.

In  addition,  as  a  condition  of  the  accelerated  approval  of  Ocaliva  for  PBC  in  the  United  States,  we  are  required  to
conduct a clinical outcomes study with respect to Ocaliva for PBC. Following discussions with regulatory authorities, we
initiated our COBALT clinical outcomes confirmatory trial for PBC in December 2014 prior to the approval of Ocaliva for
PBC. There can be no assurance that our COBALT trial conducted as part of our post-marketing obligations will confirm
that  the  surrogate  endpoint  used  for  accelerated  approval  of  Ocaliva  for  PBC  will  show  an  adequate  correlation  with
clinical outcomes.

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Changes to our Ocaliva label with respect to patients with PBC with decompensated cirrhosis (e.g., Child-Pugh Class
B  or  C),  a  prior  decompensation  event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension  influenced
modifications  to  our  COBALT  study  design  and  as  a  result  of  the  changes  to  the  U.S.  prescribing  information  we  also
removed from the trial subjects in the United States who are now excluded from the scope of the label. In addition, while
we  remain  blinded  to  safety  and  efficacy  data  in  this  trial,  the  DMC  reviewed  the  unblinded  results  of  a  pre-specified
interim efficacy analysis of the COBALT trial and reviewed unblinded safety and pharmacokinetic data. Following these
reviews,  the  DMC  stated  that  it  was  not  feasible  to  continue  the  COBALT  trial  as  designed  and  noted  the  challenges  in
enrolling and maintaining placebo-controlled post-marketing studies in this rare disease setting. No acute safety concerns
were  noted  by  the  DMC.  Given  the  feasibility  concerns  noted  by  the  DMC  and  the  potential  confounding  impact  of
subjects discontinuing treatment and/or transitioning from investigational product to commercial drug during clinical trials,
we discussed with the FDA and the EMA proposed modifications to the COBALT trial, and we notified the FDA and the
EMA of the DMC’s recommendation. Based on discussions with both the FDA and EMA, which are ongoing, we are in the
process of closing out the COBALT trial. We will continue to generate placebo controlled data from the COBALT trial as
well as data from studies utilizing real world evidence in support of a broader evidence data package, which we anticipate
submitting to the FDA and the EMA in the second half of 2022. If this data package does not support fulfillment of our
post-marketing  obligations,  we  may  not  be  able  to  maintain  our  previously  granted  marketing  approvals  of  Ocaliva  for
PBC. Similarly, if approved based on a surrogate endpoint, continued approval of OCA for other indications, or of any of
our other product candidates, may be contingent upon the verification and description of clinical benefit in confirmatory
trials.

Our  marketing  authorization  in  the  European  Union  for  Ocaliva  for  the  treatment  of  PBC  is  not  a  full  approval.
Instead,  it  is  conditional  on  the  conduct  of  certain  post-approval  studies  including  the  COBALT  trial.  Our  ability  to
maintain  conditional  marketing  authorization  of  Ocaliva  for  PBC  in  the  European  Union  is  limited  to  specific
circumstances  and  subject  to  several  conditions  and  obligations  that  we  may  be  unable  to  satisfy  in  whole  or  at  all,
including  the  completion  of  one  or  more  clinical  outcomes  trials  to  confirm  the  clinical  benefit  of  Ocaliva  for  PBC.
Conditional  marketing  authorizations  based  on  interim  clinical  data  may  be  granted  for  a  limited  number  of  listed
medicinal products for human use, including products designated as orphan medicinal products under European Union law,
if (i) the benefit-risk balance of the product is positive, (ii) it is likely that the applicant will be in a position to provide the
required comprehensive clinical trial data post-authorization, (iii) an unmet medical need will be fulfilled by the product
and (iv) the benefit to patients of the product’s immediate availability outweighs the risk inherent in the fact that additional
data  are  still  required.  Specific  obligations,  including  obligations  relating  to  the  timely  and  successful  completion  of
ongoing  or  new  studies  and  the  collection  of  pharmacovigilance  data,  may  be  specified  in  the  conditional  marketing
authorization. Conditional marketing authorizations are valid for one year, and may be renewed annually, if the benefit-risk
balance  remains  positive,  and  after  an  assessment  of  the  need  for  additional  or  modified  conditions.  Although  we  have
successfully renewed our conditional marketing authorization in the European Union in the past, there can be no assurance
that  we  will  be  able  to  continue  to  do  so  in  the  future.  Failure  to  renew  our  conditional  marketing  authorization  would
prevent us from continuing to market Ocaliva for PBC in the European Union.

Our ongoing Phase 3 REGENERATE trial of OCA in patients with liver fibrosis due to NASH incorporates an interim
primary surrogate endpoint that may serve as the basis for accelerated approval in the United States and as the basis for a
conditional  approval  in  the  European  Union.  Accelerated  approval  in  the  United  States  and  conditional  approval  in  the
European Union for OCA for liver fibrosis due to NASH are subject to similar risks as discussed above in relation to OCA
for  PBC.  In  the  primary  efficacy  analysis  of  the  REGENERATE  trial,  once-daily  OCA  25  mg  met,  with  statistical
significance, the primary endpoint agreed with the FDA of fibrosis improvement by at least one stage with no worsening of
NASH (defined as no worsening of hepatocellular ballooning, no worsening of lobular inflammation and no worsening of
steatosis) at the planned 18-month analysis. Although a numerically greater proportion of patients in both OCA treatment
groups compared to placebo achieved the primary endpoint of NASH resolution with no worsening of liver fibrosis in the
primary efficacy analysis, this result did not reach statistical significance. As agreed with the FDA, in order for the primary
objective to be met, the study was required to achieve one of the two primary endpoints. Notwithstanding the results of the
REGENERATE 18-month analysis, the CRL issued by the FDA in June 2020 indicated that, based on the data the FDA
had reviewed, the FDA had determined that the predicted benefit of OCA based on a surrogate histopathologic endpoint
remains uncertain and does not sufficiently outweigh the potential risks to support accelerated approval for the treatment of
patients with liver fibrosis due to NASH. The FDA recommended that we submit additional post-interim analysis efficacy
and safety data from the ongoing REGENERATE study in support of potential accelerated

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approval  and  that  the  long-term  outcomes  phase  of  the  study  should  continue.  Although  we  are  in  discussions  with  the
FDA with respect to the potential resubmission of our NDA seeking accelerated approval of OCA for the treatment of liver
fibrosis due to NASH, there is no assurance that we will be successful or that OCA will be approved for liver fibrosis due
to NASH on an accelerated basis, or at all. In June 2019, the FDA issued new draft guidance on the development of drugs
for  the  treatment  of  NASH  patients  with  compensated  cirrhosis.  Although  we  believe  that,  if  successful,  our  Phase  3
REVERSE trial will support a regulatory submission seeking accelerated approval of OCA for liver fibrosis due to NASH
with compensated cirrhosis in the U.S., we do not know if achievement of the primary endpoint will ultimately be found
sufficient by the FDA for approval on an accelerated basis, or at all.

While  OCA  received  breakthrough  therapy  designation  from  the  FDA  in  January  2015  for  the  treatment  of  NASH
patients with liver fibrosis and we have filed a NDA in the United States and a MAA in Europe for approval of OCA for
liver fibrosis due to NASH based on the results from the 18-month interim analysis of our Phase 3 REGENERATE trial,
we  do  not  know  if  one  pivotal  clinical  trial  will  be  sufficient  for  marketing  approval  or  if  regulatory  authorities  in  the
United States, the European Union, or any of our other target markets will approve OCA for liver fibrosis due to NASH on
an accelerated or conditional basis, or at all. There may be delays in the FDA and EMA review processes and the FDA
and/or  the  EMA  may  also  require  that  we  continue  our  Phase  3  REGENERATE  trial  until  completion  to  assess  the
potential benefits of OCA treatment on liver-related and other clinical outcomes. Our regulatory pathway for OCA for the
treatment  of  NASH  will  depend  upon  our  ongoing  discussions  with  the  FDA  and  the  EMA.  As  a  result,  we  may  face
difficulty  in  establishing  an  acceptable  registration  strategy  with  respect  to  our  Phase  3  REGENERATE  and  REVERSE
trials, as well as other trials we may conduct in other subpopulations of NASH patients.

Prior  to  any  approval  of  OCA  for  liver  fibrosis  due  to  NASH  or  OCA  for  PBC  in  jurisdictions  in  which  it  is  not
currently  approved  or  the  approval  of  our  other  product  candidates,  the  FDA,  EMA  or  other  applicable  regulatory
authorities may require additional preclinical studies and/or clinical trials, which may be expensive and time consuming to
conduct and complete. Consequently, any such requirement that we conduct additional preclinical studies or clinical trials
could materially and adversely affect our business, financial condition and results of operations. Furthermore, even if we
were to receive any such approval, any risk mitigation programs such as a REMS, and any related restrictions, limitations
and/or warnings contained in the label of our approved products could impact our commercial success in our target markets
including with respect to future revenues generated by Ocaliva.

Delays or difficulties in the commencement, enrollment and completion of our clinical trials and studies could increase
our product development costs and delay, limit or prevent us from obtaining regulatory approval for OCA and our other
product candidates.

Delays or difficulties in the commencement, enrollment and completion of our clinical trials and studies could increase
our product development costs and limit or prevent us from obtaining or maintaining regulatory approval for OCA and our
other product candidates. We are currently conducting a number of clinical trials, including our Phase 3 REGENERATE
trial of OCA in patients with liver fibrosis due to NASH through clinical outcomes in order to confirm clinical benefit and
our Phase 3 REVERSE trial of OCA for NASH patients with compensated cirrhosis. We are also conducting our CARE
trial of OCA in pediatric patients with biliary atresia as a part of an EMA-approved pediatric investigation plan (“PIP”)
supporting the conditional approval of Ocaliva for PBC. The results from these clinical trials and our other clinical trials
and studies may not be available when we anticipate and we may be required to conduct additional clinical trials or studies
not  currently  planned  in  order  for  our  product  candidates,  including  OCA  for  PBC  and  NASH,  to  be  approved  or  to
maintain  approvals  in  the  U.S.,  Europe  or  the  other  jurisdictions  in  which  our  products  are  approved.  In  addition,  our
clinical programs are subject to a number of risks and uncertainties, such as the results of other trials, patient enrollment,
safety issues or regulatory interactions that could result in a change of trial design or timing. Any delays or difficulties in
completing one of our clinical trials could increase our product development costs and limit or prevent us from obtaining or
maintaining regulatory approval. Consequently, we do not know whether our current or future clinical trials or studies of
OCA or our other product candidates will be completed on schedule, if at all.

The  commencement,  enrollment  and  completion  of  our  clinical  trials  and  studies  may  be  delayed,  suspended  or

otherwise adversely affected for a variety of reasons, including:

● our inability to obtain sufficient funds to complete or continue our clinical trials;

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● our  inability  to  reach  agreements  on  acceptable  terms  with  prospective  contract  research  organizations
(“CROs”)  and  trial  sites,  the  terms  of  which  may  be  subject  to  extensive  negotiation  and  may  vary
significantly among our various CROs and trial sites;

● clinical holds, other regulatory objections to our commencing or continuing a clinical trial or our inability to

obtain regulatory approval to commence clinical trials in countries that require such approvals;

● our discussions with the FDA, EMA or other regulatory authorities prior to, or following, the initiation of our
clinical  trials,  regarding,  among  other  matters,  the  scope  or  design  of  our  clinical  trials,  including  trial
endpoints, protocols and statistical analysis plans, and any modifications thereto;

● our  inability  to  identify  and  maintain  a  sufficient  number  of  trial  sites,  many  of  which  may  already  be
engaged in other clinical trial programs, including some that may be for the same indications targeted by our
product candidates;

● any delay in receiving results from, or failure to achieve the necessary results in, our clinical trials;

● our inability to obtain approval from institutional review boards or independent ethics committees to conduct

our clinical trials at their respective sites;

● any DMC recommendation that our clinical trials be modified, suspended or terminated due to safety, lack of

efficacy or other reasons;

● severe or unexpected drug-related adverse events experienced by patients or any determination that a clinical

trial presents unacceptable health risks;

● any  delay  in  the  performance  of  obligations  or  breach  of  the  terms  of  any  relevant  agreement  by  us,  our
current  or  future  collaborators  and  service  providers  that  have  responsibility  for  activities  related  to  the
clinical  development  of  any  of  our  product  candidates  or  investigators  conducting  clinical  trials  on  our
product candidates;

● our  inability  to  timely  manufacture,  or  obtain  from  our  contract  manufacturers,  sufficient  quantities  of  our

product candidate required for our clinical trials; and

● any difficulty recruiting, enrolling or retaining patients in our clinical trials based on, among other factors,
the  enrollment  criteria  for  our  clinical  trials,  the  rarity  of  the  disease,  the  characteristics  of  the  population
being studied, the risks of the procedures that may be required as part of the clinical trials, such as a liver
biopsy,  the  availability  of  our  products  to  patients  generally  following  the  approval  of  such  products  or
competition  from  other  clinical  trial  programs  recruiting  patients  for  the  same  indications  as  our  product
candidates.

For  example,  our  Phase  3  REGENERATE  trial  is  a  large  and  complicated  clinical  trial  in  a  disease  without  any
approved therapies and involves serial liver biopsies over many years. While we announced topline results from the 18-
month analysis of our pivotal Phase 3 REGENERATE trial in February 2019, the study is currently planned to continue
through clinical outcomes in order to confirm clinical benefit and there can be no assurance that we will retain a sufficient
number of patients in the full study cohort or complete the clinical outcomes trial in accordance with the study protocol or
on a timely basis, if at all. Enrolling and retaining patients in such trials is challenging and there can be no assurance that
we  will  complete  the  clinical  outcomes  trial  in  accordance  with  the  study  protocol  or  on  a  timely  basis,  if  at  all.  As  we
engage in other large and complicated trials and trials in advanced disease populations, we may experience a number of
challenges that may negatively affect or delay our plans and development programs.

We have in the past experienced difficulties enrolling and retaining patients enrolled in our clinical trials. Difficulties

in enrolling and retaining patients, including due to COVID-19, may delay our clinical trials or result in negative or

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inconclusive  outcomes,  and  we  or  our  collaborators  may  decide,  or  regulatory  authorities  may  require  us,  to  conduct
additional  clinical  trials  or  additional  analyses  of  existing  clinical  trials.  Any  delay  or  compromises  with  respect  to  the
validity  of  our  clinical  trials  may  have  a  material  adverse  effect  on  our  business  or  decrease  our  competitive  position
relative to other biotechnology or pharmaceutical companies with whom we compete.

In addition, if we or any of our collaborators are required to conduct additional preclinical or clinical studies or other
development work on our product candidates beyond that contemplated, our ability to obtain regulatory approval of these
product candidates and generate revenue from their sales would be similarly harmed.

Continuing threats from COVID-19, including additional waves of infections, could materially and adversely affect our
clinical trials.

COVID-19 is a global pandemic, affecting the U.S., Europe, and other countries in which we are engaged in, or plan to
engage in, clinical development activities. We continue to closely monitor the latest developments regarding the COVID-
19  pandemic  and,  together  with  our  contract  research  organizations,  study  sites  and  other  partners,  have  taken  measures
intended to minimize disruptions and protect and retain patients enrolled in our clinical trials, including, where appropriate,
the use of telemedicine, home care visits, direct delivery of investigational product and other measures. Notwithstanding
our  efforts,  some  of  the  sites  participating  in  our  clinical  trials  have  been  affected  by  site  closings  or  reduced  capacity,
particularly in regions that are experiencing heightened impact from COVID-19. While we continue to monitor the latest
developments regarding the COVID-19 pandemic closely, if there was a meaningful negative impact on the data capture or
data quality of any of our clinical trials, such trials may not be successful or we could be required to repeat, extend the
duration of, increase the size of, or otherwise modify such trials, which could prevent or significantly delay the potential
commercialization of our product candidates and require greater expenditures. We cannot at this time predict with certainty
the  scope  of  the  impact  of  COVID-19  on  our  ability  to  execute  our  clinical  trials.  We  may  experience  issues  due  to
COVID-19 that could severely impact our clinical trials, including:

● delays,  interruptions  or  difficulties  in  the  enrollment,  scheduling  and  retention  of  patients  in  our  clinical

trials;

● delays,  interruptions  or  difficulties  in  the  conduct  of  key  clinical  trial  activities,  such  as  clinical  trial  site

monitoring and inspection readiness activities;

●   trial  conduct  issues,  including  protocol  deviations  (e.g.,  failure  to  timely  collect  liver  biopsies  or  other

required laboratory data), data capture issues and data quality issues;

● delays  or  interruptions  in  the  supply  or  administration  of  investigational  product  to  patients  in  our  clinical

trials;

● delays or interruptions in the supply of necessary equipment or materials to clinical sites;

● delays  or  difficulties  obtaining  approvals  from  regulatory  authorities,  institutional  review  boards  or  ethics
committees  of  clinical  trial  protocols  and  related  clinical  documentation  (or  amendments  and  addendums
thereto);

● delays, interruptions or difficulties in clinical site initiations, including in connection with the recruitment of

clinical site investigators and clinical site staff;

● the  redeployment  of  healthcare  resources,  including  clinical  site  investigators  and  clinical  site  staff

supporting the conduct of our clinical trials, to assist in the treatment of COVID-19 patients;

● the  diversion  of  human  capital,  including  employees,  independent  contractors,  vendors  and  other  third
parties, otherwise focused on the conduct of our clinical trials due to sickness, safety concerns or government
or employer imposed travel or working restrictions;

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● new federal, state and local government regulations or guidance that require us to change the way we conduct
our clinical trials, require the interruption or termination of our clinical trials or that result in significant and
unexpected new costs;

● delays or difficulties in interactions with regulatory authorities, institutional review boards, ethics committees
and  key  consultants  and  vendors  due  to  layoffs,  temporary  leaves,  terminations  or  other  actions  limiting
available employee resources; and

● the refusal of regulatory authorities to accept clinical trial data from clinical trials that have been negatively

affected by COVID-19.

Any such delay, interruption or issue could materially and adversely affect our business, financial condition and results

of operations.

Failure can occur at any stage of clinical development. The results of earlier clinical trials are not necessarily predictive
of  future  results  and  any  product  candidate  we  or  our  collaborators  advance  through  clinical  trials,  including  OCA,
may not have favorable results in later clinical trials or receive or maintain regulatory approval.

Clinical failure can occur at any stage of clinical development. Clinical trials may produce negative or inconclusive
results,  and  we  or  our  collaborators  may  decide,  or  regulators  may  require  us,  to  conduct  additional  clinical  trials  or
preclinical  studies.  In  addition,  data  obtained  from  trials  and  studies  are  susceptible  to  varying  interpretations,  and
regulators may not interpret our data as favorably as we do, which may delay, limit or prevent regulatory approval. Success
in preclinical studies and early clinical trials does not ensure that subsequent clinical trials will generate the same or similar
results or otherwise provide adequate data to demonstrate the efficacy and safety of our product candidates. A number of
companies  in  the  pharmaceutical  industry,  including  those  with  greater  resources  and  experience  than  us,  have  suffered
significant setbacks in Phase 3 clinical trials and at other stages of clinical development, even after seeing promising results
in earlier clinical trials.

In addition, the design of clinical trials, including trial endpoints, protocols and statistical analysis plans, can determine
whether such trials will support product approvals, and flaws in the design of such trials may not become apparent until
such  trials  are  well-advanced.  We  may  be  unable  to  design  and  execute  clinical  trials  to  support  regulatory  approval.
Further, clinical trials of product candidates often reveal that it is not practical or feasible to continue development efforts.
If OCA or our other product candidates are found to be unsafe or lack sufficient efficacy for any indication, we will not be
able to obtain or maintain regulatory approval for them, and our prospects and business may be materially and adversely
affected.

There may be significant variability in the safety and/or efficacy results we see in different trials studying OCA or our
other product candidates due to numerous factors, including differences in the underlying disease being studied, changes or
differences  in  trial  protocols  or  statistical  analysis  plans,  differences  in  the  composition  of  the  patient  populations  or
clinical trial sites, differences in adherence to the dosing regimen and other aspects of the trial protocols and differences in
the rate of dropouts among clinical trial participants. We do not know whether any Phase 2, Phase 3 or other clinical trials
we or any of our collaborators may conduct on our product candidates will demonstrate consistent or adequate efficacy and
safety or result in the approval of our product candidates by regulatory authorities. If we are unable to bring any of our
current  or  future  product  candidates  to  market,  acquire  any  previously  approved  products  or  maintain  approval  for  our
approved products, our ability to create long-term stockholder value will be limited.

In December 2014, we received comprehensive datasets from the Phase 2b FLINT trial for the treatment of NASH,
which met its primary endpoint with statistical significance. In October 2015, we announced that the Phase 2 dose ranging
trial  of  OCA  in  200  adult  NASH  patients  in  Japan  conducted  by  our  former  collaborator,  Sumitomo  Dainippon,  did  not
meet  its  primary  endpoint  with  statistical  significance.  In  the  Sumitomo  Dainippon  trial,  there  was  a  dose  dependent,
although not statistically significant, increase in the percentage of OCA-treated patients compared to placebo who achieved
the primary endpoint (p = 0.053). In addition, no difference was seen in fibrosis improvement in the OCA groups compared
to placebo. The Sumitomo Dainippon Phase 2 trial involved different doses of OCA being administered to the trial subjects
than those utilized in the Phase 2b FLINT trial. Furthermore, the baseline characteristics between the patients in the

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Japanese Phase 2 dose ranging trial conducted by Sumitomo Dainippon were distinct in a number of ways from those of
the Western patients included in the Phase 2b FLINT trial.

In February 2019, we announced topline results from the 18-month analysis of our pivotal Phase 3 REGENERATE
trial  in  patients  with  liver  fibrosis  due  to  NASH.  In  the  primary  efficacy  analysis,  once-daily  OCA  25  mg  met,  with
statistical significance, the primary endpoint agreed with the FDA of fibrosis improvement by at least one stage with no
worsening of NASH (defined as no worsening of hepatocellular ballooning, no worsening of lobular inflammation and no
worsening  of  steatosis)  at  the  planned  18-month  analysis.  Although  a  numerically  greater  proportion  of  patients  in  both
OCA treatment groups compared to placebo achieved the primary endpoint of NASH resolution with no worsening of liver
fibrosis in the primary efficacy analysis, this result did not reach statistical significance. As agreed with the FDA, in order
for the primary objective to be met, the study was required to achieve one of the two primary endpoints. Notwithstanding
the results of the REGENERATE 18-month analysis, the CRL issued by the FDA in June 2020 indicated that, based on the
data  the  FDA  had  reviewed,  the  FDA  had  determined  that  the  predicted  benefit  of  OCA  based  on  a  surrogate
histopathologic  endpoint  remains  uncertain  and  does  not  sufficiently  outweigh  the  potential  risks  to  support  accelerated
approval for the treatment of patients with liver fibrosis due to NASH. The FDA recommended that we submit additional
post-interim analysis efficacy and safety data from the ongoing REGENERATE study in support of potential accelerated
approval  and  that  the  long-term  outcomes  phase  of  the  study  should  continue.  Although  we  are  in  discussions  with  the
FDA with respect to the potential resubmission of our NDA seeking accelerated approval of OCA for the treatment of liver
fibrosis due to NASH, there is no assurance that we will be successful or that OCA will be approved for liver fibrosis due
to  NASH  on  an  accelerated  basis,  or  at  all.  While  OCA  received  breakthrough  therapy  designation  from  the  FDA  in
January 2015 for the treatment of NASH patients with liver fibrosis and we filed a NDA in the United States and a MAA in
Europe for approval of OCA for liver fibrosis due to NASH based on the results from the 18-month analysis of our Phase 3
REGENERATE  trial  in  patients  with  liver  fibrosis  due  to  NASH,  we  do  not  know  if  one  pivotal  clinical  trial  will  be
sufficient for marketing approval or if regulatory authorities in the United States, the European Union, or any of our other
target  markets  will  approve  OCA  for  liver  fibrosis  due  to  NASH  on  an  accelerated  or  conditional  basis,  or  at  all.
Additionally, interim analysis results at 18 months were based on surrogate endpoints and the impact on clinical outcomes
has not been confirmed. Our Phase 3 REGENERATE trial remains ongoing through clinical outcomes for verification and
description of clinical benefit of OCA for liver fibrosis due to NASH.

Our  product  candidates  may  have  undesirable  side  effects  which  may  delay  or  prevent  marketing  approval,  or,  if
approval is received, require that our products be taken off the market or include new or additional safety warnings.
Any  such  events  may  limit  our  existing  and  future  product  sales  and  materially  and  adversely  affect  our  business,
financial condition and results of operations.

OCA  has  been  shown  to  be  a  potent  FXR  agonist.  With  the  exception  of  the  endogenous  human  bile  acid
chenodeoxycholic  acid  and  cholic  acid,  there  are  no  approved  FXR  agonists  and  the  adverse  effects  from  long-term
exposure  to  this  drug  class  are  unknown.  Unforeseen  side  effects  from  any  of  our  product  candidates,  including  OCA,
could  arise  either  during  clinical  development  or,  if  approved,  after  the  approved  product  has  been  marketed.  Serious
adverse events, including deaths, in patients taking OCA have occurred in clinical trials and in the post-marketing setting,
and  we  cannot  assure  you  that  additional  serious  adverse  events  in  patients  taking  OCA  in  clinical  trials  or  in  the  post-
marketing setting will not occur.

The most common side effects observed in clinical trials of OCA for PBC were pruritus, fatigue, headaches, nausea,
constipation  and  diarrhea.  In  our  Phase  3  POISE  trial,  pruritus,  generally  mild  to  moderate,  was  the  most  frequently
reported adverse event associated with OCA treatment for PBC and was observed in 38% of patients on placebo, 70% of
patients  in  the  OCA  10  mg  group  and  56%  of  patients  in  the  OCA  titration  group  (5  mg  to  10  mg).  Eight  patients
discontinued due to pruritus, of whom none were in the placebo group, seven (10%) were in the OCA 10 mg group and one
(1%) was in the OCA titration group. Pruritus also has been observed in other clinical trials of OCA. Decreases in high
density lipoprotein HDL cholesterol were also observed during treatment in our Phase 3 POISE trial. In our Phase 2 trials
for OCA for PBC, a dose-response relationship was observed in the occurrence of liver-related adverse reactions, including
jaundice, ascites and primary biliary cholangitis flare with dosages of OCA of 10 mg once daily to 50 mg once daily (up to
5-times the highest recommended dosage), as early as one month after starting treatment with OCA. The European label
for Ocaliva also notes that elevations in alanine amino transferase and aspartate aminotransferase were observed in patients
treated with OCA.

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In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended  weekly  dose  in  such  patients.  As  a  result,  in  September  2017,  we  issued  a  Dear  Health  Care  Provider
(“DHCP”)  letter,  and  the  FDA  also  subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended
label dosing. Both communications remind healthcare providers of the importance of the recommended reduced dosing of
Ocaliva in PBC patients with moderate or severe hepatic impairment, while reiterating the importance of monitoring PBC
patients  for  progression  of  their  disease  and  the  occurrence  of  liver-related  adverse  reactions.  In  addition  to  the  DHCP
letter,  we  took  actions  to  enhance  education  about  appropriate  use  of  Ocaliva.  These  initiatives  included:  reeducating
physicians  on  the  label,  with  a  focus  on  ensuring  appropriate  dosing  for  patients  with  moderate  or  severe  hepatic
impairment; enhancing monitoring of patients for liver-related adverse reactions; and adjudicating reported cases of serious
liver injury, including in patients with no or mild hepatic impairment. In February 2018, we announced that the Ocaliva
label in the United States had been updated by the FDA to include a boxed warning and a dosing table that reinforced the
then-existing dosing schedule for patients with Child-Pugh Class B or C or decompensated cirrhosis. In addition, the FDA
issued an updated drug safety communication to accompany the revised label. We remain focused on the safety of all of the
patients  using  Ocaliva  within  and  outside  of  our  ongoing  clinical  studies  and  have  engaged  with  relevant  regulatory
authorities  to  ensure  that  the  Ocaliva  label  sufficiently  reinforces  the  importance  of  appropriate  dosing  in  patients  with
advanced cirrhosis.

In  2020  the  FDA  notified  us  that,  in  the  course  of  its  routine  safety  surveillance,  in  May  of  that  year  it  began  to
evaluate  a  newly  identified  safety  signal,  or  NISS,  regarding  liver  disorder  for  Ocaliva  which  the  FDA  classified  as  a
potential risk, focused on a subset of the cirrhotic, or more advanced, PBC patients who had taken Ocaliva. In May 2021,
the NISS process was concluded and we aligned with the FDA on updated Ocaliva prescribing information in the United
States,  and  Ocaliva  is  now  contraindicated  for  patients  with  PBC  and  decompensated  cirrhosis,  a  prior  decompensation
event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension,  in  addition  to  the  existing  contraindication  for
complete  biliary  obstruction.  This  issue,  and  any  other  safety  concerns  associated  with  Ocaliva,  perceived  or  real,  may
adversely  affect  the  successful  development  and  commercialization  of  our  product  candidates  and  approved  products,
including Ocaliva, and materially and adversely affect our business including future revenue generated by Ocaliva.

In the 18-month analysis of our pivotal Phase 3 REGENERATE trial in patients with liver fibrosis due to NASH, the
safety population included 1,968 randomized patients who received at least one dose of investigational product (OCA or
placebo)  with  exposures  up  to  37  months.  Adverse  events  were  generally  mild  to  moderate  in  severity  and  the  most
common  were  consistent  with  the  known  profile  of  OCA.  The  frequency  of  serious  adverse  events  was  similar  across
treatment groups (11% in placebo, 11% in OCA 10 mg and 14% in OCA 25 mg), and no serious adverse event occurred in
> 1% of patients in any treatment group. There were 3 deaths in the study (2 in placebo: bone cancer and cardiac arrest and
1 in OCA 25 mg: glioblastoma) and none were considered related to treatment. The most common adverse event reported
was dose-related pruritus (19% in placebo, 28% in OCA 10 mg and 51% in OCA 25 mg). The incidence of pruritus across
all  three  treatment  groups  was  highest  in  the  first  three  months  and  decreased  thereafter.  The  large  majority  of  pruritus
events were mild to moderate, with severe pruritus occurring in a small number of patients (< 1% in placebo, < 1% in OCA
10 mg and 5% in OCA 25 mg). A higher incidence of pruritus-associated treatment discontinuation was observed for OCA
25  mg  (<  1%  in  placebo,  <  1%  in  OCA  10  mg  and  9%  in  OCA  25  mg).  According  to  the  clinical  study  protocol,
investigator  assessed  severe  pruritus  mandated  treatment  discontinuation.  Consistent  with  observations  from  previous
NASH studies, OCA treatment was associated with an increase in low density lipoprotein (“LDL”) cholesterol, with a peak
increase of 22.6 mg/dL at 4 weeks and subsequently reversing and approaching baseline at month 18 (4.0 mg/dL increase
from  baseline).  Triglycerides  rapidly  and  continually  decreased  in  the  OCA  treatment  groups  through  month  18.  There
were few and varied serious cardiovascular events and incidence was balanced across the three treatment groups (2% in
placebo, 1% in OCA 10 mg and 2% in OCA 25 mg). In patients with type 2 diabetes, OCA treatment was associated with
an early transient increase in fasting glucose and hemoglobin A1c with return to levels similar to placebo by month 6. No
clinically meaningful changes were noted in non-diabetic patients.

With  respect  to  hepatobiliary  events,  more  patients  (3%)  on  OCA  25  mg  experienced  gallstones  or  cholecystitis
compared to < 1% on placebo and 1% on OCA 10 mg. While hepatic serious adverse events were rare (< 1% incidence in
each of the three treatment groups), more occurred in the OCA 25 mg group with no pattern attributable to OCA.

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In  the  Phase  2b  FLINT  trial,  pruritus  occurred  more  frequently  in  the  OCA  treatment  group  than  in  the  placebo
treatment group (23% vs. 6%, p < 0.0001) and at a higher grade (predominately moderate pruritus). OCA treatment was
also  associated  with  changes  in  serum  lipid  levels,  including  increases  in  total  cholesterol  and  LDL  cholesterol  and  a
decrease  in  HDL  cholesterol,  that  were  observed  within  12  weeks  of  initiating  treatment,  peaked  and  then  decreased  in
magnitude while on treatment, and reversed further during the 24-week post-treatment period. These changes in cholesterol
levels,  along  with  the  achievement  of  pre-defined  efficacy  criteria,  played  a  role  in  the  decision  of  the  FLINT  data  and
safety monitoring board to terminate the treatment phase of the Phase 2b FLINT trial, and the publication of the FLINT
results noted the need for further study of these changes. There were two patient deaths in the Phase 2b FLINT trial, and
neither death was considered related to OCA treatment.

Furthermore, the Phase 2 dose ranging trial of OCA in 200 adult NASH patients in Japan conducted by our former
collaborator, Sumitomo Dainippon, did not meet statistical significance for the primary endpoint. The primary endpoint in
the Sumitomo Dainippon trial was histologic improvement defined as at least a two-point improvement in the nonalcoholic
fatty  liver  disease  activity  score  with  no  worsening  of  fibrosis.  In  this  trial,  there  was  a  dose  dependent,  although  not
statistically significant, increase in the percentage of OCA-treated patients compared to placebo who achieved the primary
endpoint (p = 0.053). In addition, no difference was seen in fibrosis improvement in the OCA groups compared to placebo.

  In  December  2015,  we  initiated  a  Phase  2  clinical  trial,  known  as  the  CONTROL  trial,  to  characterize  the  lipid
metabolic  effects  of  OCA  and  cholesterol  management  effects  of  concomitant  statin  administration  in  NASH  patients.
CONTROL enrolled 80 NASH patients who were naïve to statin therapy or had undergone a statin washout period. The
study included a 16-week double-blind phase followed by an optional long-term safety extension (“LTSE”) phase of the
trial.  OCA  treatment  in  the  absence  of  statin  therapy  over  the  first  four  weeks  resulted  in  an  increase  in  LDL  across  all
OCA treatment groups, while the placebo group was relatively unchanged. Treatment with atorvastatin beginning at week
four  and  continuing  through  week  16  reversed  OCA-related  increases  in  LDL  to  below  baseline  levels  in  all  OCA
treatment groups. Dose-dependent pruritus was the most common adverse event in patients treated with OCA, occurring in
5% of patients on placebo, 5% of patients in the OCA 5 mg group, 10% of patients in the OCA 10 mg group and 55% of
patients in the OCA 25 mg group. All adverse events were mild to moderate and two patients discontinued treatment in the
OCA 25 mg group due to pruritus. Over 95% of the patients completing the double-blind phase of CONTROL enrolled in
the LTSE phase of the trial.

During the LTSE phase of CONTROL, there was one patient death. This patient was a 64 year-old male with a history
of NASH associated liver cirrhosis, morbid obesity (BMI >40) and type 2 diabetes. At baseline, this patient had blood tests
consistent with impaired liver function (e.g., low LDL and low platelets). The patient was randomized to placebo for the
double-blind phase of the study. Early in the double-blind phase, the patient had serum biochemistry changes consistent
with  worsening  hepatic  impairment  (e.g.,  albumin  decline  and  bilirubin  was  increasing).  Atorvastatin  was  started  per
protocol  and  then  stopped  early  due  to  the  patient’s  persistently  low  LDL  levels.  The  patient  later  enrolled  in  the  LTSE
phase  and  began  receiving  OCA  25  mg  treatment.  Over  the  following  four  months,  the  patient’s  serum  biochemistry
remained  consistent  with  ongoing  hepatic  impairment.  Approximately  five  months  after  starting  the  LTSE  phase,  the
patient  developed  severe  protracted  diarrhea,  which  resulted  in  weight  loss  of  30  pounds  over  the  ensuing  one-month
period.  Both  an  infectious  cause  and  possible  inflammatory  bowel  disease  were  suspected,  and  the  patient  subsequently
was  started  on  broad  spectrum  antibiotics  and  steroid  therapy.  Due  to  the  diarrhea,  the  principal  investigator  stopped
treatment with OCA and discontinued the patient from the study. Concurrently, the patient reported jaundice and was found
to  have  significantly  elevated  serum  bilirubin  and  ALP,  while  other  liver  enzymes  remained  relatively  stable.  Over  the
ensuing  two-week  period,  various  diagnostic  tests  and  procedures  were  performed  (e.g.,  magnetic  resonance
cholangiopancreatography  to  investigate  possible  gallstone  bile  duct  obstruction)  and  the  patient  continued  receiving  a
number of other medications, including the ongoing course of steroid therapy. During this time, the patient continued to
deteriorate and was hospitalized with acute renal and liver failure, complicated by severe metabolic acidosis. The patient
rapidly  progressed  to  multi-organ  system  failure,  sepsis  and  death.  The  principal  investigator  determined  that  the  events
leading to the patient’s death were unlikely related to OCA. Despite the numerous confounding factors in this case, given
the contemporaneous administration of OCA during the patient’s ongoing deterioration, we determined that it could not be
ruled out that these events were possibly related to treatment. Subsequent to our determination, the independent data safety
monitoring  committee  separately  evaluated  the  case  and  determined  that  the  events  leading  to  the  patient’s  death  were
unlikely related to OCA.

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Additional or unforeseen side effects relating to OCA or any of our other product candidates could arise either during
clinical development or, if approved, after the approved product has been marketed. With the approval of Ocaliva for PBC
in the United States, the European Union, and certain of our other target markets, OCA is currently used in an environment
that is less rigorously controlled than in clinical studies. If new side effects are found, if known side effects are shown to be
more  severe  than  previously  observed  or  if  OCA  is  shown  to  have  other  unexpected  characteristics,  we  may  need  to
abandon our development of OCA for PBC, NASH and other potential indications. Furthermore, our commercial sales of
Ocaliva for PBC may be materially and adversely affected.

The  range  and  potential  severity  of  possible  side  effects  from  systemic  therapies  is  significant.  The  results  of  our
current or future clinical trials may show that our product candidates, including OCA, cause undesirable or unacceptable
side effects, which could interrupt, delay or halt clinical trials, result in a delay of, or failure to obtain, marketing approval
from the FDA and other regulatory authorities, result in marketing approval from the FDA and other regulatory authorities
with restrictive label warnings or result in the withdrawal of previously granted marketing approvals.

In  addition,  our  product  candidates  are  being  developed  as  potential  treatments  for  severe,  life  threatening  diseases
and,  as  a  result,  our  trials  will  necessarily  be  conducted  in  patient  populations  that  are  more  prone  than  the  general
population to exhibit certain disease states or adverse events. For example, our Phase 3 REVERSE trial in NASH patients
with  compensated  cirrhosis  has  expanded  our  NASH  development  program  into  a  more  advanced  NASH  patient
population  and  accordingly  imposes  certain  eligibility  requirements  for  uptitration,  as  well  as  certain  monitoring
requirements  thereafter.  Ocaliva  is  prescribed  in  patients  suffering  from  various  stages  of  PBC,  which  can  be  life
threatening, and patients may suffer from other concomitant illnesses that may increase the likelihood of certain adverse
events. It may be difficult to discern whether certain events or symptoms observed during our clinical trials or by patients
using our approved products are related to our product candidates or approved products or some other factor. As a result,
we and our development programs may be negatively affected even if such events or symptoms are ultimately determined
to be unlikely related to our product candidates or approved products. We cannot assure you that additional or more severe
adverse  side  effects  related  to  OCA  or  our  other  product  candidates  will  not  be  observed  in  our  clinical  trials  or  in  the
commercial  setting.  If  observed,  such  adverse  side  effects  could  delay  or  preclude  regulatory  approval  of  OCA,  limit
commercial use or result in the withdrawal of previously granted marketing approvals.

If we or others identify undesirable or unacceptable side effects caused by our product candidates or products:

● we may be required to modify, suspend or terminate our clinical trials;

● we  may  be  required  to  modify  or  include  additional  dosage  and  administration  instructions,  warnings  and
precautions,  contraindications,  boxed  warnings,  limitations,  restrictions  or  other  statements  in  the  product
label for our approved products, or issue field alerts to physicians and pharmacies or implement other risk
mitigation programs;

● we may be required to conduct costly additional clinical trials;

● we may be subject to limitations on how we may promote our approved products;

● sales of our approved products may decrease significantly;

● regulatory authorities may require us to take our approved products off the market;

● we  may  be  subject  to  regulatory  investigations,  government  enforcement  actions,  litigation  or  product

liability claims; and

● our products may become less competitive or our reputation may suffer.

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Breakthrough therapy designation for OCA may not lead to faster development or regulatory processes or increase the
likelihood that the FDA will approve OCA for the treatment of NASH patients with fibrosis.

If  a  drug  is  intended  for  the  treatment  of  a  serious  or  life-threatening  condition  and  preliminary  clinical  evidence
indicates  that  the  drug  may  demonstrate  substantial  improvement  over  existing  therapies  on  one  or  more  clinically
significant endpoints, such as substantial treatment effects observed early in clinical development, the FDA may grant a
breakthrough therapy designation. Breakthrough therapy designation is intended to facilitate the development, and expedite
the review, of such drugs, but the breakthrough therapy designation does not assure marketing approval by the FDA.

In January 2015, we received breakthrough therapy designation for OCA for the treatment of NASH patients with liver
fibrosis.  However,  there  is  no  guarantee  that  the  receipt  of  breakthrough  therapy  designation  will  result  in  a  faster
development process, review or approval of OCA for liver fibrosis due to NASH or increase the likelihood that OCA will
be granted marketing approval for NASH patients with liver fibrosis. Notwithstanding our receipt of breakthrough therapy
designation, in June 2020 we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to
NASH.  Although  we  are  in  discussions  with  the  FDA  with  respect  to  the  potential  resubmission  of  our  NDA  seeking
accelerated approval of OCA for the treatment of liver fibrosis due to NASH, there is no assurance that the outcome of
these discussions will lead to resolution of the issues identified in the CRL or that if we resubmit our NDA that it will be
approved. Similarly, any future breakthrough therapy designation relating to any other potential indication of OCA or our
other  product  candidates  will  neither  guarantee  a  faster  development  process,  review  or  approval  nor  improve  the
likelihood of the grant of marketing approval by the FDA compared to conventional FDA procedures. In addition, the FDA
may withdraw any breakthrough therapy designation at any time. While we may seek breakthrough therapy designation for
one or more of our product candidates in the future, we can give no assurance that the FDA will grant such status.

We may not be able to obtain or, if approved, maintain orphan drug exclusivity for our approved products or product
candidates, which could cause our revenues to suffer.

Regulatory  authorities  in  some  jurisdictions,  including  the  United  States  and  Europe,  may  designate  drugs  and
biologics for relatively small patient populations as orphan drugs. Under the Orphan Drug Act, the FDA may designate a
product as an orphan drug if it is a drug or biologic intended to treat a rare disease or condition, which is generally defined
as  a  patient  population  of  fewer  than  200,000  individuals  annually  in  the  United  States.  OCA  has  received  orphan  drug
designation in the United States and the European Union for the treatment of PBC and PSC.

Generally,  if  a  product  with  an  orphan  drug  designation  subsequently  receives  the  first  marketing  approval  for  the
indication for which it has such designation, the product is entitled to a period of marketing exclusivity, which precludes
the  FDA  or  the  EMA  from  approving  another  marketing  application  for  the  same  product  during  the  exclusivity  period.
The applicable exclusivity period is seven years in the United States and ten years in Europe. Orphan drug exclusivity may
be lost if the FDA or EMA determines that the request for designation was materially defective or if the manufacturer is
unable  to  assure  a  sufficient  quantity  of  the  product  to  meet  the  needs  of  patients  with  the  rare  disease  or  condition.  In
addition, the European exclusivity period can be reduced to six years if, at the end of the fifth year, it is established that the
product no longer meets the criteria for orphan drug designation because, for example, the product is sufficiently profitable
not to justify maintenance of market exclusivity.

Any failure to maintain orphan drug status may subject us to mandatory price discounts in Europe and result in the loss
of other benefits, such as tax exemptions for sales. As such, the loss of orphan drug status may have a negative effect on
our ability to successfully commercialize our products, earn revenues and achieve profitability.

Even if we obtain orphan drug exclusivity for a product, that exclusivity may not effectively protect the product from
competition because different products can be approved for the same condition. Even after an orphan drug is approved, the
FDA or EMA may subsequently approve another product for the same condition if the FDA or EMA concludes that the
later  product  is  clinically  superior  (i.e.,  it  is  shown  to  be  safer,  more  effective  or  makes  a  major  contribution  to  patient
care). Any inability to secure or maintain orphan drug status or the exclusivity benefits of this status could have a material
adverse impact on our ability to develop and commercialize our product candidates and approved products.

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We  rely  entirely  on  third  parties  for  the  manufacture  of  our  product  requirements  for  our  preclinical  studies  and
clinical trials, as well as our commercial supply of Ocaliva and, if approved, OCA for liver fibrosis due to NASH and
our  other  product  candidates,  and  also  depend  on  third-party  vendors  and  CROs  for  certain  of  our  clinical  trial  and
product development activities. Our business could be harmed if our third-party manufacturers fail to provide us with
sufficient quantities of drug product, or fail to do so at acceptable quality levels or prices, or if our third-party vendors
or  CROs  assisting  us  with  our  clinical  trials  and  product  development  activities  fail  to  comply  with  their  contractual
commitments  or  applicable  regulatory  obligations  or  if  we  lose  our  relationships  with  our  third-party  vendors  and
CROs.

We do not manufacture the pharmaceutical products that we sell or the product candidates that we are developing. We
rely  on  third-party  contract  manufacturers  for  all  of  our  required  raw  materials,  active  pharmaceutical  ingredient  and
finished product for our commercial sales and for our existing and anticipated clinical trials and preclinical studies. Any
inability by our contract manufacturers to continue to provide services to us for any reason, including due to COVID-19
and  related  public  health  safety  measures  and  business  closures  and  disruptions,  could  disrupt  the  supply  chain  for  our
pharmaceutical  products  and  product  candidates  and  materially  and  adversely  affect  our  commercialization  efforts  and
clinical development program, and we may be unable to identify, qualify and engage replacement suppliers on terms that
are favorable to us on a timely basis, if at all.

We rely on our suppliers for the manufacture and commercial supply of API for use in Ocaliva and, if approved, OCA
for  liver  fibrosis  due  to  NASH.  We  are  currently  dependent  upon  a  limited  number  of  suppliers,  with  whom  we  have
contractual  arrangements,  although  we  are  working  on  developing  further  sources  of  supply.  While  we  have  procured
supplies of API for the commercialization of Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH that
we believe will be sufficient to meet our requirements during the initial stages of a potential NASH launch, we may not be
able to procure sufficient supplies of API on an ongoing basis. If these suppliers are unable to provide adequate supply, we
may  not  be  able  to  meet  our  long-term  commercial  supply  requirements  of  API  for  the  manufacture  of  Ocaliva  or,  if
approved,  OCA  for  liver  fibrosis  due  to  NASH  or  other  indications  on  acceptable  terms,  or  at  all.  We  do  not  have
agreements  for  long-term  supplies  of  any  of  our  product  candidates  other  than  OCA.  We  currently  obtain  supplies  and
services relating to our other product candidates from our third-party contract manufacturers on a purchase order basis.

The  facilities  used  by  any  contract  manufacturer  to  manufacture  OCA  or  any  of  our  other  product  candidates  are
subject to inspection by the FDA and regulators in other jurisdictions, as are the facilities and operations of our third-party
vendors and CROs. We are completely dependent on these third-party manufacturers for compliance with the requirements
of U.S. and non-U.S. regulators for the manufacture of our finished products, including Ocaliva. If our manufacturers are
unable to meet our requirements in accordance with our product specifications and applicable current Good Manufacturing
Practices (“cGMP”) requirements, our products or product candidates will not be approved or, if already approved, may be
subject  to  recall.  In  addition,  if  COVID-19  or  related  public  health  safety  measures  prevent  the  FDA,  EMA  or  other
relevant regulators from conducting manufacturing inspections or other regulatory activities with respect to manufacturing,
it  could  significantly  impact  the  ability  of  the  FDA,  EMA  or  such  other  regulators  to  timely  review  and  process  our
regulatory submissions, which could have a material and adverse effect on our business and financial condition.

Reliance on third-party manufacturers entails risks to which we would not be subject if we manufactured our product

candidates and products ourselves, including:

● the possibility that we are unable to enter into or renew our manufacturing agreements with third parties on

acceptable terms, or at all;

● the possible termination, breach or non-performance by our third-party manufacturers of our manufacturing

agreements based on factors beyond our control; and

● our  inability  to  timely  identify  and  qualify  a  replacement  for  any  of  our  third-party  manufacturers  in  the
event any such third-party manufacturer fails to meet our product requirements or following the termination,
expiration or nonrenewal of our agreements with such third-party manufacturer.

Any of these factors could disrupt the supply of our product candidates or approved products, cause us to incur higher

costs, delay the approval of our product candidates or prevent or disrupt the commercialization of our approved products.

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Furthermore,  if  any  of  our  product  candidates,  including  OCA  for  liver  fibrosis  due  to  NASH,  are  approved  and  our
contract manufacturers fail to deliver the required commercial quantities of API or finished product on a timely basis and at
commercially reasonable prices and we are unable to find one or more replacement manufacturers capable of production at
a substantially equivalent cost, in substantially equivalent volumes and quality and on a timely basis, we would likely be
unable  to  meet  demand  for  such  product  candidate  following  its  approval  and  could  lose  potential  revenue.  It  may  take
several  years  to  establish  an  alternative  long-term  source  of  supply  and  to  have  any  such  new  source  approved  by  the
regulatory authorities that regulate our products in the United States, the European Union and our other target markets.

We depend on third-party vendors and CROs for certain of our clinical trial and product development activities. If any
of  these  providers  fail  to  comply  with  their  contractual  commitments  or  applicable  regulatory  obligations,  including  the
completion  of  deliverables  in  a  timely  manner  and  in  accordance  with  acceptable  quality  standards,  including  due  to
COVID-19  and  related  public  health  safety  measures  and  business  closures  and  disruptions,  our  business  could  be
materially and adversely affected. In addition, if we are unable to maintain our relationship with any one or more of these
providers, we could experience a significant delay in both identifying another comparable provider and then contracting for
its  services,  which  could  materially  and  adversely  affect  our  clinical  trial  and  product  development  efforts.  We  may  be
unable to retain an alternative provider on reasonable terms, or at all. Even if we locate an alternative provider, it is likely
that  such  a  provider  will  need  additional  time  to  respond  to  our  needs  and  may  not  provide  the  same  type  or  level  of
services  as  the  original  provider.  Any  third-party  vendors  and  CROs  that  we  retain  are  subject  to  the  FDA’s  regulatory
requirements  and  similar  foreign  standards  and  we  do  not  have  control  over  compliance  with  these  regulations  by  these
providers. The FDA, EMA and other relevant regulatory authorities enforce these regulations through periodic inspections
of trial sponsors, principal investigators and trial sites. If these regulations are not adhered to by these providers, or if such
providers fail to timely correct any non-compliance, or if COVID-19 or related public health safety measures prevent the
FDA,  EMA  or  other  relevant  regulatory  authorities  from  conducting  inspections  or  other  regulatory  activities,  the
commercialization  and  development  of  our  product  candidates  or  approved  products  could  be  delayed,  which  could
materially and adversely harm our business and financial condition.

Even though we have received conditional approval of Ocaliva for PBC, we and our contract manufacturers are still
subject to strict, ongoing regulatory requirements.

Even though we have received conditional approval of Ocaliva for the treatment of PBC in combination with UDCA
in adults with an inadequate response to UDCA or as monotherapy in adults unable to tolerate UDCA, we and our contract
manufacturers  are  subject  to  ongoing  regulatory  requirements  relating  to,  among  other  things,  Ocaliva’s  manufacturing,
packaging, labeling and storage. In addition, we and our contract manufacturers and our contract manufacturers’ facilities
are  required  to  comply  with  extensive  FDA  and  EMA  requirements  and  the  requirements  of  other  similar  regulatory
authorities, including requirements that quality control and manufacturing procedures conform to current cGMPs. As such,
we and our contract manufacturers are subject to periodic cGMP inspections and other inspections and audits required by
law  or  industry  standard  and  must  continue  to  expend  time,  money  and  effort  to  ensure  compliance  with  applicable
manufacturing, production and quality control requirements. We are also required to report certain adverse reactions and
production  problems,  if  any,  to  the  FDA,  EMA  and  other  similar  regulatory  authorities  and  to  comply  with  certain
requirements  concerning  advertising  and  promotion  for  our  products.  Promotional  communications  with  respect  to
prescription  drugs  are  subject  to  a  variety  of  legal  and  regulatory  restrictions  and  generally  must  be  consistent  with  the
information in the product’s approved label.

If a regulatory authority such as the FDA identifies previously unknown problems with one of our products, such as
adverse events of unanticipated severity or frequency or problems with the facility where the product is manufactured, or
disagrees with the promotion, marketing or labeling of one of our products, it may impose restrictions on that product or
us, including requiring withdrawal of the product from the market. In addition, if we or our contract manufacturers, other
third-party  vendors  or  collaborators  fail  to  comply  with  applicable  regulatory  requirements,  a  regulatory  agency  may,
among other things:

● issue Form 483 notices or Warning Letters, in the case of the FDA, or similar notices, in the case of other

regulatory agencies;

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● mandate  modifications  to  our  promotional  materials  or  require  us  to  provide  corrective  information  to

healthcare practitioners;

● require us or our collaborators to enter into a consent decree or permanent injunction, which may include the
imposition of various fines, reimbursements for inspection costs, required due dates for specific actions and
penalties for noncompliance;

● recall our products;

● suspend any of our ongoing clinical studies;

● impose administrative, civil or criminal penalties;

● withdraw regulatory approval or require changes to our product label, including the inclusion of additional

warnings or changes to the approved indication;

● refuse  to  approve  pending  applications  or  supplements  to  approved  applications  filed  by  us  or  our

collaborators;

● impose  restrictions  on  our  operations  or  those  of  our  contract  manufacturers,  including  costly  new

manufacturing requirements; or

● seize or detain products.

Risks Related to the Commercialization of Our Products

Sales of Ocaliva may be adversely affected by safety and labeling changes required by regulators.

In  the  course  of  our  post-marketing  pharmacovigilance  activities,  deaths  have  been  reported  in  PBC  patients  with
moderate or severe hepatic impairment. In an analysis performed by us and in consultation with the FDA, we concluded
that  certain  of  these  patients  were  prescribed  once  daily  doses  of  Ocaliva,  which  is  seven  times  higher  than  the
recommended weekly dose in such patients. As a result, in September 2017, we issued a DHCP letter and the FDA also
subsequently  issued  its  own  drug  safety  communication  to  reinforce  recommended  label  dosing.  Both  communications
remind  healthcare  providers  of  the  importance  of  the  recommended  reduced  dosing  of  Ocaliva  in  PBC  patients  with
moderate  or  severe  hepatic  impairment,  while  reiterating  the  importance  of  monitoring  PBC  patients  for  progression  of
their disease and the occurrence of liver-related adverse reactions. In February 2018, we announced that the Ocaliva label
in the United States had been updated by the FDA to include a boxed warning and a dosing table that reinforced the then-
existing  dosing  schedule  for  patients  with  Child-Pugh  Class  B  or  C  or  decompensated  cirrhosis.  In  addition,  the  FDA
issued an updated drug safety communication to accompany the revised label. We remain focused on the safety of all of the
patients  using  Ocaliva  within  and  outside  of  our  ongoing  clinical  studies  and  have  engaged  with  relevant  regulatory
authorities  to  ensure  that  the  Ocaliva  label  sufficiently  reinforces  the  importance  of  appropriate  dosing  in  patients  with
advanced cirrhosis.

In  2020  the  FDA  notified  us  that,  in  the  course  of  its  routine  safety  surveillance,  in  May  of  that  year  it  began  to
evaluate  a  newly  identified  safety  signal,  or  NISS,  regarding  liver  disorder  for  Ocaliva  which  the  FDA  classified  as  a
potential risk, focused on a subset of the cirrhotic, or more advanced, PBC patients who had taken Ocaliva. In May 2021,
the NISS process was concluded and we aligned with the FDA on updated Ocaliva prescribing information in the United
States,  and  Ocaliva  is  now  contraindicated  for  patients  with  PBC  and  decompensated  cirrhosis,  a  prior  decompensation
event,  or  compensated  cirrhosis  with  evidence  of  portal  hypertension,  in  addition  to  the  existing  contraindication  for
complete  biliary  obstruction.  This  issue,  and  any  other  safety  concerns  associated  with  Ocaliva,  perceived  or  real,  may
adversely  affect  the  successful  development  and  commercialization  of  our  product  candidates  and  approved  products,
including Ocaliva, and materially and adversely affect our business including future revenue generated by Ocaliva.

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Regulators  other  than  the  FDA  where  Ocaliva  is  approved  and/or  commercialized,  including  the  EMA,  may  also

require safety and labeling changes.

We are subject to uncertainty relating to pricing and reimbursement. Failure to obtain or maintain adequate coverage,
pricing and reimbursement for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future
approved products, if any, could have a material adverse impact on our ability to commercialize such products.

The availability and extent of coverage and reimbursement from governmental and private healthcare payors for our
products,  including  Ocaliva  for  PBC  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH,  and  our  ability  to  obtain
adequate pricing for such products are key factors that will affect our future commercial prospects. Government authorities
and third-party payors, such as private health insurers and health maintenance organizations, decide which drugs they will
cover  and  establish  payment  levels.  Sales  of  our  products  depend  and  will  depend  substantially,  both  domestically  and
internationally, on the extent to which their cost will be paid by health maintenance, managed care, pharmacy benefit and
similar healthcare management organizations or reimbursed by government health administration authorities, private health
coverage  insurers  and  other  third-party  payors.  Accordingly,  the  coverage  and  reimbursement  decisions  of  such
governmental and private healthcare payors could reduce the demand for, or the price paid for, our products. If these payors
do  not  consider  our  products  to  be  cost-effective  alone,  or  relative  to  other  approved  therapies,  they  may  not  cover  our
products or, if they do, they may apply utilization management restrictions, high patient cost-sharing obligations, or restrict
the level of reimbursement.

Third-party payors are increasingly challenging the prices charged for pharmaceuticals products, and many also limit
reimbursement for newly-approved products and indications. Third-party payors often attempt to contain healthcare costs
by  demanding  price  discounts  or  rebates  and  limiting  both  the  types  and  variety  of  drugs  that  they  will  cover  and  the
amounts that they will pay for drugs. As a result, they may not provide adequate payment for our products. Similarly, the
containment of healthcare costs has become a priority for federal and state governments and the pricing of pharmaceutical
products  has  been  a  focus  in  this  effort.  The  U.S.  government,  state  legislatures  and  foreign  governments  have  shown
significant  interest  in  implementing  cost-containment  programs,  including  price  controls,  restrictions  on  reimbursement,
requirements  for  substitution  of  generic  products  and  requirements  to  demonstrate  a  specific  degree  of  improvement  in
terms of medical benefit compared to existing therapies. Adoption of price controls and cost-containment measures, and
adoption of more restrictive policies in jurisdictions with existing controls and measures, could adversely affect our ability
to successfully commercialize our products. In addition, we may be required to conduct post-marketing studies in order to
demonstrate  the  cost-effectiveness  of  our  products  to  payors’  satisfaction.  Such  studies  might  require  us  to  commit  a
significant amount of management’s time and our financial and other resources and our products might not ultimately be
considered cost-effective.

We  do  not  know  if  Ocaliva  for  PBC  will  obtain  and  maintain  broad  acceptance  from  third-party  payors  in  the
jurisdictions in which it is, or may in the future be, approved. In addition, even if OCA for liver fibrosis due to NASH is
approved,  we  do  not  know  if  it  will  obtain  and  maintain  broad  acceptance  from  third-party  payors.  The  coverage
determination process is a time-consuming and costly process that requires us to provide scientific and clinical support for
the  use  of  Ocaliva  for  PBC  and,  if  approved,  OCA  for  liver  fibrosis  due  to  NASH  to  each  payor  separately,  with  no
assurance  that  coverage  will  be  obtained  or  maintained.  The  market  for  a  drug  depends  significantly  on  access  to  third-
party payors’ drug formularies, or lists of medications for which third-party payors provide coverage and reimbursement.
Third-party payors may refuse to include a particular drug in their formularies or restrict patient access to a branded drug
when a less costly generic equivalent or other alternative is available, even if not approved for the indication for which the
branded  drug  is  approved.  Due  to  there  being  no  uniform  policy  of  coverage  and  reimbursement  in  the  United  States
among commercial payors, coverage and reimbursement for pharmaceutical products may differ significantly from payor
to payor. If we are unable to obtain and maintain adequate coverage from third-party payors, the adoption of Ocaliva for
PBC and, if approved, OCA for liver fibrosis due to NASH by physicians and patients may be limited. This in turn could
affect our ability to successfully commercialize Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH and
have a material adverse impact our profitability, results of operations, financial condition and future success.

We cannot be certain that we will be able to obtain and maintain adequate coverage, pricing and reimbursement for our
products,  including  Ocaliva  for  PBC,  OCA  for  liver  fibrosis  due  to  NASH,  if  approved,  or  our  other  future  approved
products, if any. If coverage or reimbursement is not available or is available on a limited basis, or if we are unable to

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obtain and maintain adequate pricing, we may not be able to successfully commercialize Ocaliva for PBC, OCA for liver
fibrosis due to NASH, if approved, or our other future approved products, if any.

In February 2022, ICPT France withdrew its application for reimbursement in France of Ocaliva for treatment of PBC,
on account of inability to reach mutually acceptable pricing terms with CEPS. ICPT France initiated sales of Ocaliva in
France  prior  to  finalization  of  reimbursement  terms  pursuant  to  an  ATU.  ICPT  France  will  continue  to  work  with  the
French regulators regarding ATU and post-ATU payback. In France, prior to reaching mutually acceptable pricing terms,
the pharmaceutical company has discretion in setting prices, which are paid by CEPS. CEPS retains the ability to request
payback  later  if  it  determines  that  the  appropriate  price  is  lower  than  the  price  charged  at  the  time.  Disagreements  with
regulators  over  pricing  or  payback  terms  can  negatively  affect  our  business,  up  to  and  including  withdrawal  from  the
relevant  jurisdiction.  We  have  reserved  for  potential  partial  payback  of  past  French  revenues  based  on  pre-withdrawal
correspondence received from the French regulator, but the French government may seek a higher payback amount than we
have reserved.

Legislative and regulatory healthcare reform may adversely affect our business.

In  the  United  States,  the  Medicare  Prescription  Drug,  Improvement,  and  Modernization  Act  of  2003  (the  “MMA”)
changed  the  way  Medicare  covers  and  pays  for  pharmaceutical  products.  The  legislation  established  Medicare  Part  D,
which  expanded  Medicare  coverage  for  outpatient  prescription  drug  purchases  by  the  elderly  but  provided  authority  for
limiting the number of drugs that will be covered in any therapeutic class. The MMA also introduced a new reimbursement
methodology  based  on  average  sales  prices  for  physician-administered  drugs.  Any  negotiated  prices  for  our  products
covered by a Part D prescription drug plan will likely be lower than the prices we might otherwise obtain. Moreover, while
the MMA applies only to drug benefits for Medicare beneficiaries, private payors often follow Medicare coverage policy
and  payment  limitations  in  setting  their  own  payment  rates.  Any  reduction  in  payment  that  results  from  the  MMA  may
result in a similar reduction in payments from non-governmental payors.

In  March  2010,  the  Patient  Protection  and  Affordable  Care  Act,  as  amended  by  the  Health  Care  and  Education
Affordability  Reconciliation  Act  (collectively,  the  “ACA”),  became  law  in  the  United  States.  Among  other  things,  the
purpose of the ACA was to reduce the cost of healthcare and substantially change the way healthcare is financed by both
governmental and private insurers. The ACA requires discounts under the Medicare drug benefit program and increased
the rebates paid by pharmaceutical companies on drugs covered by Medicaid. The ACA also imposes an annual fee, which
increases each year, on sales by branded pharmaceutical manufacturers. The ACA has been challenged repeatedly in court,
and its future is uncertain. If the ACA is ultimately overturned or repealed, the effect on our business could be material.

Reimbursement in the European Union and many other territories must be negotiated on a country-by-country basis
and  in  many  countries  a  product  cannot  be  commercially  launched  until  reimbursement  is  approved.  The  timing  to
complete the negotiation process in each country is highly uncertain. Even after a price is negotiated, countries frequently
request or require adjustments to the price and other concessions over time or require approvals regionally. Reimbursement
agencies (payors) in Europe are often more conservative than those in the United States and the reimbursement process is
often slower since reimbursement decisions are made on a country-by-country basis and may involve multiple government
agencies in a given country. Prices for drugs in Europe are generally lower than in the United States and tend to decrease
over time. In February 2022, ICPT France withdrew its application for reimbursement in France of Ocaliva for treatment of
PBC on account of inability to reach mutually acceptable pricing terms with CEPS.

The United States and several other jurisdictions are considering, or have already enacted, a number of legislative and
regulatory proposals to change their healthcare systems in ways that could affect our ability to sell our products profitably.
Among policy makers and payors in the United States and elsewhere, there is significant interest in promoting changes in
healthcare  systems  with  the  stated  goals  of  containing  healthcare  costs,  improving  quality  and/or  expanding  access  to
healthcare.  In  the  United  States,  the  pharmaceutical  industry  has  been  a  particular  focus  of  these  efforts  and  has  been
significantly affected by major legislative initiatives. We expect to experience pricing pressures in connection with the sale
of  Ocaliva  and  our  other  future  approved  products,  if  any,  due  to  the  trend  toward  managed  healthcare,  the  increasing
influence of health maintenance organizations and additional legislative proposals. Pricing pressures recently experienced
by the pharmaceutical industry may be further exacerbated by legislative and policy changes proposed or considered by the
executive branch and the United States Congress. In addition, it is possible that additional governmental action is taken

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to address pricing concerns arising in connection with COVID-19. We cannot predict the success or impact of any such
current or future federal or state legislative efforts.

Ocaliva and our other future approved products, if any, may not achieve broad market acceptance among physicians,
patients and healthcare payors, and revenues generated from their sales may be limited as a result.

The commercial success of Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, and our other future
approved products, if any, will depend upon their acceptance among the medical community, including third-party payors,
healthcare providers and professionals and customers, including patients and patient advocacy groups. In order for Ocaliva
to be commercially successful for PBC, we need to demonstrate its utility as a cost-effective treatment for PBC patients
who have an inadequate response to UDCA or who are unable to tolerate UDCA. Ocaliva also must be shown to be a safe
and  tolerable  treatment  in  a  commercial  use  setting  as  it  is  intended  to  be  a  lifetime  therapy  for  patients  eligible  for
treatment. We cannot be certain that Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future
approved  products,  if  any,  will  achieve  an  adequate  level  of  acceptance  among  the  medical  community,  including
physicians, healthcare payors and patients.

In addition, we continue to closely evaluate the impact of COVID-19 on our ability to effectively market, sell and

distribute Ocaliva for PBC. The long-term effects of COVID-19 are unknown.

The degree of market acceptance of our approved products depends on a number of factors, including:

● limitations,  warnings,  precautions,  boxed  warnings,  contraindications,  restrictions  or  other  statements
contained in the product labels of our products, or any risk mitigation programs such as a REMS required for
our products by the FDA, EMA or other relevant regulatory authorities;

● changes in the standard of care or availability of alternative therapies at similar or lower costs for the targeted

indications for any of our products, such as UDCA for the treatment of PBC;

● limitations in the approved indications for our products;

● demonstrated and perceived clinical safety and efficacy compared to competitive products;

● a lack of adverse side effects, including deaths and other serious adverse events;

● sales, marketing and distribution support;

● the availability of reimbursement from managed care plans and other third-party payors;

● the timing of the market introduction of competitive products;

● the degree of cost-effectiveness;

● availability of alternative therapies at similar or lower cost, including generic and over-the-counter products;

● the  extent  to  which  our  products  are  approved  for  inclusion  on  formularies  of  hospitals  and  managed  care

organizations;

● whether  and  to  what  extent  our  products  are  recommended  under  physician  treatment  guidelines  for  the

treatment of the indications for which we have received regulatory approval;

● adverse publicity concerning our products or favorable publicity concerning competitive products;

● the convenience and ease of administration of our products;

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● potential product liability claims; and

● the effects of COVID-19 and related public health safety measures and business closures and disruptions.

In addition, the potential market opportunity for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved,
and our other future approved products, if any, is difficult to precisely estimate. For example, our estimates of the potential
market opportunity for Ocaliva for PBC include a number of key assumptions related to prevalence rates, patients’ access
to healthcare, diagnosis rates and patients’ response to or tolerance of Ocaliva, which are based on available literature and
epidemiology  research  in  PBC,  our  industry  knowledge  gained  through  market  research  and  other  methods,  industry
publications, third-party research reports and other surveys. While we believe that our internal assumptions are reasonable,
no independent source has verified such assumptions. If any of these assumptions prove to be inaccurate, then the actual
market for Ocaliva for PBC could be smaller than our estimates of our potential market opportunity. If the actual market
opportunity for Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future approved products,
if any, is smaller than we expect, our product revenue may be limited and our financial condition and results of operations
may be materially and adversely affected.

If Ocaliva for PBC, OCA for liver fibrosis due to NASH, if approved, or our other future approved products, if any, do

not achieve an adequate level of acceptance among the medical community, including physicians, healthcare payors and
patients, sufficient revenue may not be generated from these products and we may not become or remain profitable. In
addition, our efforts to educate the medical community and third-party payors on the benefits of Ocaliva for PBC, OCA for
liver fibrosis due to NASH, if approved, and our other future approved products, if any, may require significant resources
and may never be successful.

We could incur significant liability if it is determined that we have improperly promoted or are improperly promoting
Ocaliva for PBC or any of our product candidates prior to their approval.

Physicians are permitted to prescribe drug products for uses that are not described in the product’s labeling and that
differ from those approved by the FDA or other applicable regulatory agencies. Off-label uses are common across medical
specialties. Although the FDA and other regulatory agencies do not regulate a physician’s choice of treatments, the FDA
and other regulatory agencies do restrict communications on the subject of off-label use. Companies are not permitted to
promote  drugs  in  a  manner  inconsistent  with  applicable  regulatory  guidance.  The  FDA,  the  U.S.  Department  of  Justice
(“DOJ”) and other regulatory and enforcement authorities actively enforce laws and regulations prohibiting the improper
promotion of approved products, as well as the promotion of products for which marketing approval has not been obtained.
A company that is found to have improperly promoted off-label uses will be subject to significant liability, including civil
and  administrative  remedies  as  well  as  criminal  sanctions.  A  significant  number  of  pharmaceutical  companies  have
received inquiries or been the subject of investigations by various governmental authorities in the United States and abroad.
Both federal and state governments have levied large civil and criminal fines against companies for alleged improper off-
label promotion, as well as promotion that is determined to be false or misleading, even if related to approved indications.

While we have implemented a corporate compliance program based on what we believe are current best practices, we
cannot provide any assurance that governmental authorities, including the DOJ, SEC or FDA, will find that our business
practices  comply  with  all  current  or  future  administrative  or  judicial  interpretations  of  potentially  applicable  laws  and
regulations.  In  addition,  government  and  regulatory  agencies  may  hold  us  responsible  for  any  actions  by  our  sales
representatives and other employees or contingent workers to the extent that they do not comply with applicable laws and
regulations.  If  we  fail  to  comply  with  any  of  these  laws  and  regulations,  we  could  be  subject  to  a  range  of  penalties,
including  the  issuance  of  an  untitled  letter,  a  warning  letter,  injunction,  seizure,  criminal  and  significant  civil  penalties,
fines, damages, disgorgement, curtailment or restructuring of our operations, exclusion, disqualification or debarment from
participation in federally- or state-funded healthcare programs or other sanctions or litigation, any of which could have a
material adverse impact on our business, financial condition and results of operations.

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If  we  market  products  in  a  manner  that  violates  healthcare  fraud  and  abuse  laws,  or  if  we  violate  government  price
reporting or physician payment disclosure laws, we may be subject to civil or criminal penalties.

In addition to FDA restrictions on the marketing of pharmaceutical products, several other types of state and federal
healthcare  laws,  commonly  referred  to  as  “fraud  and  abuse”  laws,  have  been  applied  in  recent  years  to  restrict  certain
marketing practices in the pharmaceutical industry. Other jurisdictions including Europe have similar laws and are enacting
more  stringent  regulations.  These  laws  include  false  claims  and  anti-kickback  statutes.  It  is  possible  that  some  of  our
business activities could be subject to challenge under one or more of these laws.

Federal  false  claims  laws  generally  prohibit  anyone  from  knowingly  and  willingly  presenting,  or  causing  to  be
presented, any claims for the payment for goods (including drugs) or services to third-party payers (including Medicare and
Medicaid) that are false or fraudulent. The federal civil monetary penalties statute, likewise, imposes penalties against any
person or entity that, among other things, is determined to have presented or caused to be presented a claim to a federal
health program that the person knows or should know is for an item or service that was not provided as claimed or is false
or fraudulent.

The federal healthcare program anti-kickback statute prohibits, among other things, knowingly and willfully offering,
paying,  soliciting  or  receiving  remuneration  to  generate  business,  including  the  purchase  or  prescription  of  a  particular
product covered by Medicare, Medicaid or other federally financed healthcare programs. This statute has been interpreted
to apply to arrangements between pharmaceutical manufacturers on the one hand and prescribers, purchasers or formulary
managers  on  the  other.  Although  there  are  several  statutory  exemptions  and  regulatory  safe  harbors  protecting  certain
common  activities  from  prosecution,  the  exemptions  and  safe  harbors  are  drawn  narrowly,  and  practices  that  involve
remuneration intended to induce prescribing, purchasing or recommending may be subject to scrutiny if they do not qualify
for an exemption or safe harbor. In addition, such exemptions and safe harbors are subject to change from time to time.

The Health Insurance Portability and Accountability Act of 1996 (as amended by the Health Information Technology
for  Economic  and  Clinical  Health  Act,  “HIPAA”)  created  additional  federal  criminal  statutes  that  prohibit,  among  other
things, knowingly and willfully executing, or attempting to execute, a scheme to defraud any healthcare benefit program,
or obtain, by means of false or fraudulent pretenses, or promises, any of the money or property owned by, or under the
custody or control of, any healthcare benefit program, regardless of the payor (e.g., public or private) and knowingly and
willfully  falsifying,  concealing  or  covering  up  by  any  trick  or  device  a  material  fact  or  making  any  materially  false
statement, in connection with the delivery of, or payment for, healthcare benefits, items or services. HIPAA also imposes
significant requirements on the receipt and transfer of protected health information.

In  addition,  the  federal  transparency  requirements  under  the  Physician  Payments  Sunshine  Act  require  certain
manufacturers of drugs, including us, for which payment is available under certain federal healthcare programs annually to
report  information  related  to  payments  and  other  transfers  of  value  to  physicians  and  teaching  hospitals,  and  physician
ownership and investment interests.

Finally, we must offer discounted pricing or rebates on Ocaliva and our future approved products, if any, under various
federal and state healthcare programs, and report specific prices to government agencies under healthcare programs. The
calculations necessary to determine the prices reported are complex and the failure to report prices accurately may expose
us to significant penalties.

There  are  foreign  and  state  law  equivalents  of  these  laws  and  regulations,  such  as  anti-kickback,  false  claims,
transparency and data privacy and security laws, to which we are currently and/or may in the future be subject. We may
also  be  subject  to  foreign  and  state  laws  that  require  manufacturers  to  report  information  related  to  payments  and  other
transfers of value to physicians and other healthcare providers or marketing expenditures. Many of these laws differ from
each other in significant ways, thus increasing the cost and complexity of our compliance efforts.

A number of pharmaceutical and other healthcare companies have been prosecuted under these laws for a variety of
promotional and marketing activities, including providing free trips, free goods, sham consulting fees and grants and other
monetary benefits to prescribers; reporting inflated average wholesale prices that were then used by federal programs to

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set reimbursement rates; engaging in improper promotional activities; and submitting inflated best price information to the
Medicaid Drug Rebate Program to reduce liability for Medicaid rebates.

If  we  or  our  operations  are  found  to  be  in  violation  of  any  of  the  laws  described  above  or  any  other  governmental
regulations  that  apply  to  us,  we  may  be  subject  to  penalties,  including  criminal  and  significant  civil  penalties,  damages,
fines, imprisonment, exclusion of products from reimbursement under United States federal or state healthcare programs,
and the curtailment or restructuring of our operations. Any penalties, damages, fines, curtailment or restructuring of our
operations  could  materially  and  adversely  affect  our  ability  to  operate  our  business  and  our  financial  results.  Although
compliance programs can mitigate the risk of investigation and prosecution for violations of these laws, the risks cannot be
entirely eliminated. Any action against us for violation of these laws, even if we successfully defend against it, could cause
us to incur significant legal expenses and divert our management’s attention from the operation of our business. Moreover,
achieving and sustaining compliance with these laws may prove costly.

We  may  not  be  successful  in  establishing,  implementing  and  maintaining  development  and  commercialization
collaborations, which could adversely affect our ability to develop certain of our product candidates and our financial
condition  and  operating  results.  If  any  strategic  collaborator  fails  to  perform  its  obligations  under,  or  terminates,  its
agreement with us, our business could be substantially harmed.

Developing  pharmaceutical  products,  conducting  clinical 

trials,  obtaining  regulatory  approval,  expanding
manufacturing capabilities and marketing approved products are expensive, complex and time-consuming undertakings. As
a result, we have in the past entered into, and may in the future seek to enter into, collaborations with third parties upon
whom we may rely for financial resources and for development, regulatory and commercialization expertise for selected
products  or  product  candidates  and  in  selected  jurisdictions.  We  may  establish  collaborations  with  respect  to  the
development and commercialization of OCA in various jurisdictions and for our other product candidates. Additionally, we
may enter into sales and marketing arrangements with third parties with respect to our approved products in all or certain
jurisdictions.

Our collaborators may fail to develop our product candidates or effectively commercialize our products for a variety of
reasons, including a lack of sufficient resources, a decision not to devote the necessary resources due to internal constraints,
such  as  limited  cash  or  human  resources,  a  change  in  strategic  focus  or  a  failure  to  obtain  the  necessary  regulatory
approvals.

If we are unable to enter into new arrangements or maintain such arrangements on acceptable terms, or at all, we may
be  unable  to  effectively  market  and  sell  our  products  in  certain  of  our  target  markets.  We  expect  to  face  competition  in
seeking appropriate collaborators. Moreover, collaboration and similar arrangements are complex and time consuming to
negotiate, document and implement and they may require substantial resources to maintain. We may not be successful in
our efforts to establish and implement collaborations or other alternative arrangements for the development of our product
candidates.  When  we  collaborate  with  a  third  party  for  development  and  commercialization  of  a  product  candidate  or
approved product, we expect to relinquish some or all of the control over the future success of that product candidate or
approved  product  to  the  third  party.  Our  collaboration  partner  may  not  devote  sufficient  resources  to  development  or
commercialization  or  may  otherwise  fail  in  their  development  or  commercialization.  The  terms  of  any  collaboration  or
other arrangement that we establish may not be favorable to us. In addition, any collaboration that we enter into may be
unsuccessful.  In  some  cases,  we  may  be  responsible  for  continuing  preclinical  and  initial  clinical  development  of  a
partnered  product  candidate  or  research  program,  and  the  payment  we  receive  from  our  collaboration  partner  may  be
insufficient to cover the cost of this development. If we are unable to reach agreements with suitable collaborators, we may
incur increased costs and we may be forced to limit the number of products or product candidates we can commercially
develop  or  the  territories  in  which  we  can  commercialize  them.  If  we  fail  to  achieve  successful  collaborations,  our
operating results and financial condition could be materially and adversely affected.

If we fail to develop OCA for additional indications such as NASH, our commercial opportunity will be limited.

To date, we have focused the majority of our development efforts on the development of OCA. One of our strategies is
to pursue clinical development of OCA for liver fibrosis due to NASH and other progressive non-viral liver diseases, to the
extent that we have sufficient funding to do so.

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PBC is an orphan disease and the potential market size for Ocaliva for PBC is relatively limited. Furthermore, because
a  significant  proportion  of  PBC  patients  do  not  exhibit  any  symptoms  at  the  time  of  diagnosis,  PBC  may  be  left
undiagnosed for a significant period of time. Due to these factors, our ability to grow revenues will be dependent on our
ability  to  increase  market  share  and  successfully  develop  and  commercialize  OCA  for  the  treatment  of  additional
indications. In particular, we believe that our future success will depend in large part on the results of our development of
OCA  for  the  treatment  of  NASH.  Although  NASH  is  believed  to  be  one  of  the  most  prevalent  chronic  liver  diseases
worldwide,  NASH  may  be  left  undiagnosed  in  patients  for  a  long  period  of  time  and  a  definitive  diagnosis  of  NASH  is
often  based  on  a  histological  assessment  of  a  liver  biopsy,  which  impacts  the  ability  to  easily  identify  patients.
Furthermore,  even  if  we  are  successful  in  developing  and  obtaining  marketing  approval  of  OCA  for  the  treatment  of
NASH, we may not be commercially successful.

The completion of development, securing of approval and commercialization of OCA for additional indications such
as liver fibrosis due to NASH will require substantial additional funding, is subject to numerous risks and we may not be
successful.  We  cannot  provide  you  any  assurance  that  we  will  be  able  to  successfully  advance  any  of  these  indications
through the development process. Even if we receive regulatory approval to market OCA for the treatment of liver fibrosis
due  to  NASH  or  any  other  additional  indications,  we  cannot  assure  you  that  any  such  additional  indications  will  be
successfully  commercialized,  widely  accepted  in  the  marketplace  or  more  effective  than  other  commercially  available
alternatives.  If  we  are  unable  to  successfully  develop  and  commercialize  OCA  for  liver  fibrosis  due  to  NASH  or  other
additional indications, our commercial opportunity will be limited and our business prospects will suffer.

Risks Related to Our Business and Strategy

We depend on third-party contractors for a substantial portion of our operations and may not be able to control their
work as effectively as if we performed these functions ourselves.

We outsource and plan to continue to outsource substantial portions of our operations to third-party service providers,
including  CROs  for  certain  of  our  clinical  trial  and  product  development  activities,  and  contract  manufacturers  for  the
production of API and finished drug product for our commercial sales, clinical trials and preclinical studies. We will likely
also use the services of third-party vendors in connection with our future commercialization activities, including product
sales,  marketing  and  distribution.  Our  agreements  with  third-party  service  providers  are  typically  on  a  study-by-study
and/or  project-by-project  basis.  Typically,  we  may  terminate  these  agreements  with  notice  and  are  responsible  for  the
supplier’s previously incurred costs. In addition, a number of third-party service providers that we retain will be subject to
the FDA’s and EMA’s regulatory requirements and similar standards outside of the United States and Europe and we do not
have  control  over  compliance  with  these  regulations  by  these  providers.  If  these  providers  do  not  adhere  to  applicable
governing  practices  and  standards,  the  commercialization  of  Ocaliva  and  our  other  approved  products,  if  any,  and  the
development  of  OCA  and  our  other  product  candidates  could  be  delayed  or  stopped,  which  could  severely  harm  our
business and financial condition.

Because we have relied on third parties, our internal capacity to perform these functions is limited. Outsourcing these
functions involves the risk that third parties may not perform to our standards, may not produce results in a timely manner
or  may  fail  to  perform  at  all.  In  addition,  the  use  of  third-party  service  providers  requires  us  to  disclose  our  proprietary
information to these parties, which could increase the risk that this information will be misappropriated. There are a limited
number  of  third-party  service  providers  that  have  the  specialized  expertise  required  to  achieve  our  business  objectives.
Identifying, qualifying and managing the performance of third-party service providers can be difficult, time-consuming and
cause delays in our development programs. Despite our growth, we have limited internal resources available to identify and
monitor  third-party  service  providers.  To  the  extent  we  are  unable  to  identify,  retain  and  successfully  manage  the
performance of third-party service providers, our business may be materially and adversely affected. We may further be
subject to the imposition of civil or criminal penalties if our third party service providers violate applicable law.

Our third-party service providers generally are not prohibited from providing their services to other biopharmaceutical
companies,  including  companies  that  currently  or  may  in  the  future  compete  with  us.  For  example,  certain  of  our  third-
party service providers and consultants may be able to develop intellectual property to which we do not have rights under
our  agreements  and  that  may  eventually  be  used  to  develop  products  that  compete  with  our  products.  Although  we
generally have confidentiality and non-disclosure agreements in place with our third-party service providers and

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consultants,  such  third  parties  may  be  able  to  provide  services  to  other  companies  without  violating  the  terms  of  our
agreements. In addition, although we may seek to enter into non-compete arrangements with our key third-party service
providers,  such  arrangements  are  difficult  to  negotiate  and  we  may  be  unable  to  successfully  enter  into  or  enforce  such
arrangements.

The  effects  of  COVID-19  and  related  public  health  safety  measures  and  business  closures  and  disruptions  may
negatively  impact  our  and  our  third-party  service  providers’  productivity,  limit  the  conduct  of  business  operations  and
impair our and our third-party service providers’ ability to conduct operations.

We  face  rapid  technological  change  and  competition  from  other  biotechnology  and  pharmaceutical  companies.  Our
operating results will suffer if we fail to compete effectively.

The  biotechnology  and  pharmaceutical  industries  are  intensely  competitive  and  subject  to  rapid  and  significant
technological  change.  We  have  competitors  in  the  United  States,  Europe  and  other  jurisdictions,  including  major
multinational pharmaceutical companies, established biotechnology companies, specialty pharmaceutical and generic drug
companies and universities and other research institutions. Many of our competitors have financial, sales and marketing,
manufacturing and distribution, legal, regulatory and product development resources substantially greater than ours. Large
pharmaceutical  companies,  in  particular,  have  extensive  experience  in  research,  clinical  testing,  obtaining  regulatory
approvals, recruiting patients and manufacturing pharmaceutical products. These companies also have significantly greater
sales  and  marketing  capabilities  and  often  have  collaborative  arrangements  in  our  target  markets.  Established
pharmaceutical companies may also invest heavily to accelerate discovery and development of novel compounds or to in-
license novel compounds that could make our products or product candidates obsolete. As a result of all of these factors,
our competitors may succeed in obtaining patent protection and/or FDA, EMA or other regulatory approval or discovering,
developing  and  commercializing  drugs  for  the  diseases  that  we  are  targeting  before  we  do.  Smaller  or  early-stage
companies  may  also  prove  to  be  significant  competitors,  particularly  through  collaborative  arrangements  with  large,
established companies. See “Item 1. Business—Our Product Candidates—Competition”.

Off-label uses of other potential treatments may limit the commercial potential of our products and product candidates,
especially given the pricing of Ocaliva and the anticipated pricing for our product candidates. For example, while fibrates
are  not  approved  for  use  in  PBC,  off-label  use  of  fibrate  drugs  has  been  reported.  In  NASH,  a  number  of  treatments,
including  vitamin  E  (an  antioxidant),  insulin  sensitizers  (e.g.,  metformin,  pioglitazone),  antihyperlipidemic  agents  (e.g.,
gemfibrozil), pentoxifylline and UDCA, are used off-label. Although none of these treatments have been clearly shown in
clinical trials to alter the course of the disease, in a previous study conducted by the NASH Clinical Research Network,
improvements in certain histological measures of NASH were reported with vitamin E and pioglitazone.

We believe that our ability to successfully compete will depend on, among other things:

● the results of our and our strategic collaborators’ clinical trials and preclinical studies;

● our ability to recruit, enroll and retain patients for our clinical trials;

● the  efficacy,  safety  and  tolerability  of  Ocaliva,  OCA  for  liver  fibrosis  due  to  NASH,  if  approved,  and  our

other future approved products, if any;

● the speed at which we develop our product candidates;

● our ability to design and successfully execute appropriate clinical trials;

● our ability to maintain productive relationships with regulatory authorities;

● the timing and scope of regulatory approvals, if any;

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● our ability to commercialize and market Ocaliva, OCA for liver fibrosis due to NASH, if approved, and our

other future approved products, if any;

● the price of our products;

● our  ability  to  obtain  adequate  levels  of  reimbursement  under  private  and  governmental  health  insurance

plans, including Medicare;

● our ability to protect our intellectual property rights related to our products;

● our ability to manufacture and sell commercial quantities of Ocaliva, OCA for liver fibrosis due to NASH, if

approved, and our other future approved products, if any, to the market; and

● the acceptance of our products by physicians and other healthcare providers.

If our competitors market products that are more effective or safe or less expensive than our products or that reach the
market sooner than our products, we may not achieve commercial success. In addition, the biopharmaceutical industry is
characterized  by  rapid  technological  change.  Because  our  research  approach  integrates  many  technologies,  it  may  be
difficult for us to stay abreast of the rapid changes in other technologies. If we fail to stay at the forefront of technological
change, we may be unable to compete effectively. Technological advances or products developed by our competitors may
render our technologies, products or product candidates obsolete, less competitive or not economical.

A  variety  of  risks  associated  with  our  international  business  operations  and  our  planned  international  business
relationships could materially and adversely affect our business.

We  have  formed  a  number  of  subsidiaries  in  jurisdictions  outside  of  the  United  States  in  connection  with  or  in
anticipation of our commercial or other business activities in those jurisdictions. We are commercializing Ocaliva for PBC
using  a  combination  of  our  internal  commercial  organization  and  third-party  distributors,  depending  on  the  jurisdiction.
Our  variety  of  international  operations  and  business  relationships  subject  us  to  additional  risks  that  may  materially  and
adversely affect our business and ability to attain or sustain profitability, including:

● the  enhanced  anti-bribery  and  anti-corruption  regimes  now  implemented  in  most  European  countries  and
elsewhere,  including  the  UK  Bribery  Act  and  the  escalation  of  investigations  and  prosecutions  pursuant  to
such laws;

● compliance with complex import and export control laws;

● restrictions on direct investments by foreign entities and country-specific trade restrictions;

● differing  regulatory  requirements  for  medicine  approvals  and  access  to  medicines  across  our  various
international markets and as a result the potential inability to obtain any necessary foreign regulatory, pricing
or reimbursement approvals for our products in a timely manner, or at all;

● variances  in  payment  terms  and  uncertainty  regarding  the  collectability  of  accounts  receivable  from  our

counterparties in our international business;

● difficulties in staffing and managing international operations;

● the potential for reduced protection for our intellectual property rights;

● the potential for third-party patent rights in countries outside of the United States;

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● cross border trade of medicines by third parties within the European single market (for example the impact of

parallel trade within the European Economic Area);

● unexpected changes in tariffs, trade barriers and regulatory requirements and the imposition of governmental

controls;

● economic  weakness,  including  inflation,  or  political  instability,  particularly  in  non-U.S.  economies  and

markets, including countries in Europe;

● compliance  with  tax,  employment,  immigration  and  labor  laws  applicable  to  our  employees  working  or

traveling abroad;

● compliance with data protection laws, including regimes relating to cross-border transfer mechanisms;

● taxes in other countries;

● foreign currency fluctuations, which could result in increased operating expenses and reduced revenue, and

other transactional risks incident to doing business in foreign countries;

● potential  for  production  shortages  resulting  from  events  affecting  raw  material  supply  or  manufacturing

capabilities abroad;

● business  interruptions  resulting  from  geo-political  actions,  including  war  and  terrorism,  global  health
catastrophes,  such  as  COVID-19,  natural  disasters,  including  earthquakes,  volcanoes,  typhoons,  floods,
hurricanes and fires, or social unrest; and

● increasingly  complex  standards  for  complying  with  international  laws  and  regulations  that  may  differ

substantially from country to country and may conflict with corresponding U.S. laws and regulations.

In February 2022, ICPT France withdrew its application for reimbursement in France of Ocaliva for treatment of PBC,
on account of inability to reach mutually acceptable pricing terms with CEPS. We could be adversely affected by French
regulatory actions, or operational disruptions, particularly in relation to the one-year transition period, maintaining French
staff and operations, or a request to pay back revenues from past sales.

Since the United Kingdom referendum on European Union membership in June 2016, there has been some political
and  economic  uncertainty,  including  in  the  regulatory  framework  applicable  to  the  operations  of  biotechnology  and
pharmaceutical companies, and this uncertainty may persist now that the impact of Brexit is being realized. There may be
disruption  and  uncertainties  in  the  free  movement  of  goods,  services  and  people  between  the  United  Kingdom  and  the
European Union, and at a more detailed level disruption to, and uncertainty regarding the application and interpretation of,
national  and  international  laws  and  regulations.  There  is  now  additional  process  and  documentation  required  to  move
goods  between  the  United  Kingdom  and  the  European  Union,  and  we  and  our  third-party  supply  chain  partners  may
experience  delays,  disruptions,  and  increased  costs  as  a  result.  There  may  also  be  unforeseen  consequences  and
uncertainties in cross border trade in goods and services, immigration and employment, data protection and digital trade,
state aid and fair competition. Over the last few years our international business has undertaken significant planning and
operational readiness work for Brexit involving business functions such as supply chain, quality, finance/tax, regulatory,
pharmacovigilance and legal. Brexit could materially change the regulatory regime applicable to our operations, including
with respect to Ocaliva for PBC and, if approved, OCA for liver fibrosis due to NASH and our other product candidates.
Such  consequences  and  uncertainties  could  make  it  more  difficult  and  expensive  for  us  to  do  business,  complicate  our
clinical, manufacturing and regulatory strategies and impair our ability to obtain and maintain regulatory approval for, and,
if approved, commercialize, our products and product candidates in Europe. In addition, our ability to continue to conduct
our international (ex-U.S.) operations out of the United Kingdom, where the headquarters for our international operations
is located, may be materially and adversely affected. While we have undertaken a number of Brexit-related

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contingency  planning  initiatives,  we  cannot  make  any  assurances  regarding  the  extent  to  which  our  business  may  be
adversely affected thereby.

In  addition,  we  are  subject  to  the  anti-bribery  and  anticorruption  laws  of  the  United  States  (both  those  affecting
domestic operations, and those affecting foreign operations, including the U.S. Foreign Corrupt Practices Act), as well as
of foreign jurisdictions where we operate, including the UK Bribery Act. Generally, these laws prohibit paying or offering
anything of value to a foreign government official for the purpose of obtaining or retaining business but they can also have
a much wider, extraterritorial scope, as is the case with the UK Bribery Act, and include requesting, receiving, or accepting
anything  of  value  with  the  intention  of  obtaining  an  improper  advantage,  as  well  as  include  commercial  bribery  (i.e.,
private  sector  rather  than  public  sector  bribery).  U.S.  and  foreign  regulators  have  increased  their  enforcement  of  anti-
bribery  and  anticorruption  laws  in  recent  years,  and  failure  to  comply  with  these  laws  could  result  in  various  adverse
consequences, including:

● the possible delay in approval or refusal to approve our product candidates;

● recalls, seizures or withdrawal from the market of an approved product;

● disruption in the supply or availability of our products or suspension of export or import privileges;

● the imposition of civil or criminal sanctions;

● the prosecution of executives overseeing our international operations; and

● damage to our reputation.

Any significant impairment of our ability to develop our product candidates or sell our approved products outside of

the United States could adversely impact our business and financial results.

Our  business  and  operations  would  suffer  in  the  event  of  system  failures  or  security  or  data  breaches  due  to  cyber-
attacks, or cyber intrusions, including ransomware, phishing attacks and other malicious intrusions.

In recent years, cybersecurity threats have become a greater risk and focus for companies. In particular, ransomware
attacks, where a hacker locks and threatens to delete or disclose the victim’s data unless a ransom is paid, has become a
major  risk.  We  and  our  third-party  service  providers  are  at  risk  of  cyber-attacks  or  cyber  intrusions  via  the  Internet,
computer viruses, break-ins, malware, ransomware, phishing attacks, hacking, denial-of-service attacks or other attacks and
similar  disruptions  from  the  unauthorized  use  of,  or  access  to,  computer  systems  (including  from  internal  and  external
sources).  These  types  of  incidents  continue  to  be  prevalent  and  pervasive  across  industries,  including  in  our  industry.  In
addition, we expect information security risks to continue to increase due to the proliferation of new technologies and the
increased sophistication and activities of organized crime, hackers, terrorists and other external parties, including foreign
state actors.

We are increasingly dependent on information technology systems and infrastructure, including mobile technologies,
to  operate  our  business.  In  the  ordinary  course  of  our  business,  we  collect,  process,  store  and  transmit  large  amounts  of
confidential  information,  including  intellectual  property,  proprietary  business  information  and  personal  information.  It  is
critical  that  we  do  so  in  a  secure  manner  to  maintain  the  confidentiality  and  integrity  of  such  information.  The  size  and
complexity  of  our  information  technology  systems,  and  those  of  third-party  vendors  with  whom  we  contract,  and  the
volume of data we retain, make such systems potentially vulnerable to breakdown, malicious intrusion, security breaches,
ransomware, phishing, and other cyber-attacks. Our information security systems and those of our third-party vendors are
subject  to  laws  and  regulations,  or  may  become  subject  to  new  laws  and  regulations,  requiring  that  we  enact  certain
measures to protect the privacy and security of certain information we collect or use in our business. A security breach or
privacy violation that leads to disclosure or modification of, or prevents access to, personal information or other protected
information, whether caused by internal or external parties, could harm our reputation, compel us to comply with federal
and/or state breach notification laws and foreign law equivalents, subject us to notification requirements under certain

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agreements  with  third  parties,  subject  us  to  mandatory  corrective  action,  require  us  to  verify  the  correctness  of  database
contents  and  otherwise  subject  us  to  liability  under  laws  and  regulations  that  protect  personal  information,  resulting  in
increased  costs  or  loss  of  revenue.  Similarly,  the  loss  or  unauthorized  disclosure  of  clinical  trial  data  from  completed,
ongoing  or  planned  clinical  trials  could  prevent  us  from  obtaining  regulatory  approval  or  delay  our  regulatory  approval
efforts and significantly increase our costs to recover or reproduce the data.

If we are unable to prevent such security breaches or privacy violations or implement satisfactory remedial measures,
our operations could be disrupted, and we may suffer negative impact to our reputation, financial loss and be subject to
regulatory fines and penalties. In addition, breaches and other unauthorized data access can be difficult to detect, and any
delay  in  identifying  them  may  lead  to  increased  harm  of  the  type  described  above.  Moreover,  the  reliance  on  remote
working  technologies  by  our  employees  and  third-party  partners  due  to  COVID-19  and  related  public  health  safety
measures and the prevalent use of mobile devices that access confidential and personal information increases the risk of
data security breaches, which could lead to the loss of confidential information, personal information, trade secrets or other
intellectual property. As cyber threats continue to evolve, we may be required to expend significant additional resources to
continue  to  modify  or  enhance  our  protective  measures  or  to  investigate  and  remediate  any  information  security
vulnerabilities.  While  we  have  implemented  security  measures  to  protect  our  data  security  and  information  technology
systems,  such  measures  may  not  prevent  such  events.  Significant  disruptions  of  our  information  technology  systems  or
breaches of data security could have a material adverse effect on our business, financial condition and results of operations.

We are subject to various data protection laws and our business and operations would suffer in the event of violations of
these laws.

In  the  United  States,  numerous  federal  and  state  laws,  including,  without  limitation,  HIPAA,  state  security  breach
notification  laws,  state  health  information  privacy  laws  and  federal  and  state  consumer  protection  laws,  govern  the
collection, use, disclosure and storage of personal information as well as consumer rights with regard to such information.
For example, California passed the California Consumer Privacy Act of 2018, which became effective on January 1, 2020,
and the California Privacy Rights Act will become effective in January 2023, giving California consumers further privacy
rights, largely aligned with EU privacy rights. Other states, including Virginia and Colorado, have enacted similar privacy
laws. Various foreign countries where we may process personal information also have, or are developing, privacy and data
protection laws governing the collection, use, disclosure and storage of personal information.

In July 2016, U.S. and European Commission officials adopted a framework called the European Union-U.S. Privacy
Shield (the “EU Privacy Shield”) to govern transfers of personal data from the European Economic Area (“EEA”) to the
U.S. We adopted the European Union-U.S. Privacy Shield and have certified to its requirements since October 2016. We
also adopted the Swiss-U.S. Privacy Shield (the “Swiss Privacy Shield”) in order to legitimize the transfer of personal data
from Switzerland to the U.S. In May 2018, the General Data Protection Regulation (the “GDPR”) took effect in the EEA.
The  GDPR  imposes  more  stringent  data  protection  requirements,  and  provides  for  greater  penalties  for  noncompliance,
than previous EEA data protection legislation. In addition, although we have implemented certain measures as a result of
Brexit to allow for the transfer of personal data between EEA member states and the United Kingdom, we may need to
develop additional mechanisms to permit for the transfer of this data. Implementation of the GDPR and other changes in
privacy  and  data  protection  laws  or  regulations  could  require  changes  to  certain  of  our  business  practices,  thereby
increasing  our  costs.  While  we  continue  to  engage  in  activities  to  comply  with  the  GDPR  requirements  and  other  data
protection laws, we may be unsuccessful in these efforts.

On July 16, 2020, the Court of Justice of the European Union (“CJEU”) invalidated the EU Privacy Shield as a data
transfer  mechanism  for  transferring  personal  data  from  the  EEA  to  the  U.S.,  effective  immediately.  On  September  20,
2020, the Swiss Federal Data Protection and Information Commissioner invalidated the Swiss Privacy Shield. Therefore,
the EU Privacy Shield and the Swiss Privacy Shield no longer qualify as appropriate safeguards for the transfer of personal
data from the EEA or Switzerland to the U.S. and transfers made under those frameworks could attract regulatory scrutiny
and  penalties  for  non-compliance.  There  was  no  “grace  period”  to  allow  organizations  to  implement  an  alternative  data
transfer  mechanism  to  the  EU  Privacy  Shield  and  the  Swiss  Privacy  Shield.  While  the  European  Commission  approved
Standard Contractual Clauses (“SCCs”) and Binding Corporate Rules remain valid mechanisms to transfer personal data to
third countries outside the EEA and Switzerland, the CJEU's ruling has also imposed enhanced due diligence obligations
on organizations acting as data exporters and relying on SCCs to ensure that the laws of the country to which personal data

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is  transferred  offers  a  level  of  data  protection  that  is  essentially  equivalent  to  the  EEA.  On  June  4,  2021,  the  European
Commission adopted new SCCs more aligned with the requirements of the GDPR and to be used when personal data is
transferred  outside  of  the  European  Union.  On  June  28th,  2022,  the  EU  Commission  granted  “adequacy”  to  the  UK,
allowing the free flow of EU resident personal data from the EU to recipients located in the UK. However, due to the UK’s
withdrawal from the EU, the new SCCs are not valid for transfers of UK resident personal data to countries outside of the
UK. The UK Information Commissioner’s Office has issued its own set of interim SCCs to facilitate such transfers. We are
in the process of updating our contracts with the new UK SCCs, as applicable. To the extent we are not able to employ
suitable  data  transfer  mechanisms,  including  the  implementation  of  the  new  SCCs,  to  facilitate  international  transfers  of
data, our ability to conduct our business may be materially adversely impacted.

The  legislative  and  regulatory  landscape  for  privacy  and  data  protection  continues  to  evolve,  and  there  has  been  an
increasing  amount  of  focus  on  privacy  and  data  protection  issues  that  may  affect  our  business.  There  is  a  degree  of
uncertainty associated with the legal and regulatory environment around privacy and data protection laws, which continue
to develop in ways we cannot predict, including with respect to evolving technologies, such as cloud computing. Privacy
and data protection laws may be interpreted and applied inconsistently from country to country and impose inconsistent or
conflicting requirements. As a result, our practices may not comply in the future with all such privacy and data protection
laws. Varying jurisdictional requirements could increase the costs and complexity of compliance or require us to change
our  business  practices  in  a  manner  adverse  to  our  business.  A  determination  that  we  have  violated  any  privacy  or  data
protection  laws  could  result  in  significant  damage  awards,  fines  and  other  penalties  that  could,  individually  or  in  the
aggregate,  materially  harm  our  business  and  reputation.  For  example,  administrative  fines  of  up  to  the  greater  of  €20
million  or  4%  of  our  global  turnover  may  be  imposed  for  breaches  of  the  GDPR.  We  may  also  be  liable  should  any
individual  who  has  suffered  financial  or  non-financial  damage  arising  from  our  infringement  of  the  GDPR  or  other
applicable data protection laws exercise his or her right to receive compensation against us.

In addition, our marketing activities and the marketing activities of any third parties on which we rely are subject to
various regulations, including privacy and data protection laws, consumer protection laws and competition laws. Such laws
may impair our ability, or the ability of third parties on which we rely, to collect information. Such regulations may have a
negative effect on businesses and may increase the potential civil liability and cost of operating our business.

We have significantly expanded our operations and plan to continue our expansion to support our future development
strategy for OCA for indications other than PBC, including liver fibrosis due to NASH. We may experience difficulties
in managing our significant growth.

We  have  significantly  expanded  our  operations,  including  the  size  of  our  employee  base,  as  we  pursue  our  future
development and commercialization strategy. As we advance our preclinical and clinical development programs for OCA
and  our  other  product  candidates,  seek  regulatory  approval  in  the  United  States  and  elsewhere  and  pursue  our
commercialization strategy, we may need to increase our product development, scientific, commercial and administrative
headcount.  Such  an  evolution  may  impact  our  strategic  focus  and  our  deployment  and  allocation  of  resources.  Our
management, personnel and systems may experience difficulty in adjusting to our growth and strategic focus.

We  may  also  anticipate  needs  for  growth  that  do  not  materialize.  For  example,  we  expanded  our  commercial
organization in anticipation of a potential U.S. commercial launch of OCA for liver fibrosis due to NASH. However, in
June 2020, we received a CRL from the FDA with respect to our NDA for OCA for liver fibrosis due to NASH. Although
we are in discussions with the FDA with respect to the potential resubmission of our NDA seeking accelerated approval of
OCA for the treatment of liver fibrosis due to NASH, there is no assurance that we will be successful or that OCA will be
approved for liver fibrosis due to NASH on an accelerated basis, or at all. In August 2020, we adopted the 2020 Workforce
Plan  to  reduce  our  workforce  in  light  of  the  receipt  of  the  CRL  from  the  FDA.  The  2020  Workforce  Plan  sought  to
streamline  our  operations  and  reduce  operating  expenses,  while  maintaining  the  critical  resources  needed  to  continue  to
support the NASH and PBC clinical programs, pursue the approval of OCA for the treatment of liver fibrosis due to NASH
and support our successful PBC business. The 2020 Workforce Plan resulted in a workforce reduction of approximately
25%,  or  approximately  170  employees.  The  2020  Workforce  Plan  was  implemented  during  the  third  quarter  of  2020,
immediately after its announcement, and was completed in the beginning of 2021. We can provide no assurance that we
will  correctly  forecast  the  needs  for  growth  given  our  reliance  on  approvals  from  regulatory  authorities  for  our  product
candidates.

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In addition, in order to continue to meet our obligations as a public company and to support any longer-term growth,
we may need to maintain and possibly increase our general and administrative capabilities. We have formed a number of
subsidiaries  in  key  markets  outside  of  the  United  States.  In  addition  to  our  U.S.  offices,  we  have  an  office  in  London,
which  serves  as  the  headquarters  for  our  international  (ex-U.S.)  operations,  and  regional  offices  in  a  number  of  other
countries, and we may further expand our geographical footprint in the future. Our management, personnel and systems
may  not  be  adequate  to  support  this  future  growth.  Furthermore,  we  may  face  a  number  of  complexities,  such  as  being
subject to national collective bargaining agreements for employees, in some of the countries in which we operate.

Our need to effectively manage our operations, growth and various projects requires that we:

● successfully attract and recruit new employees or consultants with the expertise and experience we require in

the United States, Europe and other jurisdictions;

● develop, expand or adjust our commercial infrastructure;

● manage our clinical programs effectively, which are often conducted at numerous domestic and international

clinical sites, and advance our other development efforts; and

● continue to improve our operational, financial and management controls, reporting systems and procedures.

If we are unable to successfully manage our growth and the increased complexity of our operations, our business may

be materially and adversely affected.

We  may  not  be  able  to  manage  our  business  effectively  if  we  are  unable  to  attract  and  retain  key  personnel  and
consultants.

We  may  not  be  able  to  attract  or  retain  qualified  personnel  and  consultants  due  to  the  intense  competition  for  such
individuals  among  biotechnology,  pharmaceutical  and  other  businesses  and  our  industry  has  experienced  a  high  rate  of
turnover  of  management  personnel  in  recent  years.  If  we  are  not  able  to  attract  and  retain  necessary  personnel  and
consultants  to  accomplish  our  business  objectives,  we  may  experience  constraints  that  will  significantly  impede  the
achievement  of  our  development  and  commercial  objectives,  our  ability  to  raise  additional  capital  and  our  ability  to
implement our business strategy.

We have experienced a high rate of turnover of management personnel in recent years. We are highly dependent on the
development, regulatory, commercialization and business development expertise of the members of our executive team, as
well as other key employees and consultants. If we lose one or more of our executive officers or other key employees or
consultants, our ability to implement our business strategy successfully could be seriously harmed. Any of our executive
officers or other key employees or consultants may terminate their employment at any time and replacing such individuals
may  be  difficult  and  time-consuming  because  of  the  limited  number  of  individuals  in  our  industry  with  the  necessary
breadth of skills and experience. Competition to hire and retain employees and consultants from this limited pool is intense,
and we may be unable to hire, train, retain or motivate such individuals.

We  also  have  key  advisors  and  consultants  who  assist  us  in  operating  our  business.  These  advisors  are  not  our
employees  and  may  have  commitments  to,  or  consulting  or  advisory  contracts  with,  other  entities  that  may  limit  their
availability to us and such individuals typically will not enter into non-compete agreements with us. If a conflict of interest
arises between their work for us and their work for another entity, we may lose their services. In addition, our advisors may
assist other companies that compete with us.

Our  employees  may  engage  in  misconduct  or  other  improper  activities,  including  noncompliance  with  regulatory
standards and requirements and insider trading, which could significantly harm our business.

We are exposed to the risk of employee fraud or other misconduct. Misconduct by employees could include intentional

failures to comply with the regulations of the FDA, the SEC or other domestic or foreign regulators, provide accurate

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information to the FDA, the SEC or other domestic or foreign regulators, comply with healthcare fraud and abuse laws and
regulations  in  the  United  States  and  abroad,  report  financial  information  or  data  accurately  or  disclose  unauthorized
activities to us. In particular, sales, marketing and business arrangements in the healthcare industry are subject to extensive
regulation in the United States and abroad intended to prevent fraud, misconduct, kickbacks, self-dealing and other abusive
practices.  Such  laws  and  regulations  may  restrict  or  prohibit  a  wide  range  of  pricing,  discounting,  marketing  and
promotion,  sales  commission,  customer  incentive  and  other  business  arrangements.  Employee  misconduct  could  also
involve the improper use of information obtained in the course of clinical trials, which could result in regulatory sanctions
and serious harm to our reputation. Misconduct and misappropriation of confidential information by our employees or third
parties  may  also  include  improper  trading  in  our  securities,  which  may  harm  our  reputation  and  result  in  enforcement
actions against us. We have adopted a global code of business conduct and implemented a corporate compliance program,
but it is not always possible to identify and deter employee misconduct, and the precautions we take to detect and prevent
this  activity  may  not  be  effective  in  controlling  unknown  or  unmanaged  risks  or  losses  or  in  protecting  us  from
governmental inquires, investigations or other actions or lawsuits stemming from a failure to comply with applicable laws
or regulations. The outcome of any such inquiry, investigation, action or lawsuit could have a significant negative impact
on our business, including as a result of the imposition of significant fines or other sanctions. In addition, the institution of
any such inquiry, investigation, action or lawsuit could negatively impact the market price of our securities.

We face potential product liability exposure, and if successful claims are brought against us, we may incur substantial
liability for our products or product candidates and may have to limit or suspend their use.

The use of our product candidates in clinical trials and the sale of any products for which we have obtained or may
obtain  marketing  approval,  such  as  Ocaliva  for  PBC,  expose  us  to  the  risk  of  product  liability  claims.  Product  liability
claims  may  be  brought  against  us  or  our  collaborators  by  participants  enrolled  in  our  clinical  trials,  patients,  healthcare
providers  or  others.  If  we  cannot  successfully  defend  ourselves  against  any  such  claims,  we  may  incur  substantial
liabilities. Regardless of their merit or eventual outcome, product liability claims may result in:

● withdrawal of clinical trial participants;

● termination of clinical trial sites or entire clinical trial programs;

● costs of related litigation;

● substantial monetary awards to patients or other claimants;

● decreased demand for our products and loss of revenues;

● impairment of our business reputation;

● diversion of management and scientific resources from our business operations; and

● the  inability  to  develop  and  commercialize  our  products  and  product  candidates  or  the  withdrawal  of  our

products from the market.

We have obtained limited product liability insurance coverage. Our insurance coverage may not reimburse us or may
not  be  sufficient  to  reimburse  us  for  any  expenses  or  losses  we  may  suffer.  Moreover,  insurance  coverage  is  becoming
increasingly expensive, and, in the future, we may not be able to maintain insurance coverage at a reasonable cost or in
sufficient amounts to protect us against losses due to product liability. Large judgments have been awarded in class action
lawsuits based on the unanticipated side effects of drug products. A successful product liability claim or series of claims
brought  against  us,  particularly  if  judgments  exceed  our  insurance  coverage,  could  decrease  our  cash  resources  and
adversely affect our business.

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Risks Related to Our Intellectual Property

It is difficult and costly to protect our proprietary rights, and we may not be able to ensure their protection. If our patent
position does not adequately protect our products such as Ocaliva and product candidates such as OCA for liver fibrosis
due to NASH, others may compete against us more directly, which could harm our business, possibly materially.

Our commercial success will depend in part on our ability to obtain and maintain patent, trademark and trade secret
protection covering Ocaliva, OCA for liver fibrosis due to NASH, if approved, and our other product candidates, as well as
our ability to successfully defend our intellectual property against third-party challenges. Our ability to stop third parties
from  making,  using,  selling,  offering  to  sell  or  importing  our  products  is  dependent  upon  the  extent  to  which  we  have
regulatory  exclusivity  or  intellectual  property-based  exclusivity  rights  under  valid  and  enforceable  patents  or  other
intellectual property that cover our products. If we fail to obtain and maintain adequate intellectual property protection, we
may  not  be  able  to  prevent  third  parties  from  launching  generic  versions  of  our  products,  from  using  our  proprietary
technologies  or  from  marketing  products  that  are  very  similar  or  identical  to  ours.  For  example,  we  have  received
paragraph  IV  certification  notice  letters  from  six  generic  drug  manufacturers  indicating  that  each  such  company  has
submitted to the FDA an ANDA seeking approval to manufacture and sell a generic version of our 5 mg and 10 mg dosage
strengths  of  Ocaliva  (obeticholic  acid)  for  PBC  prior  to  the  expiration  of  certain  patents  protecting  Ocaliva.  We  have
initiated patent infringement suits against each of these generic drug manufacturers in the United States District Court for
the  District  of  Delaware.  While  we  intend  to  vigorously  defend  and  enforce  our  intellectual  property  rights  protecting
Ocaliva, we can offer no assurance as to when the lawsuits will be decided, or whether the lawsuits will be successful. If a
generic equivalent of Ocaliva is approved and enters the market before the expiration of our patents protecting Ocaliva, our
business  may  be  materially  and  adversely  affected.  See  Note  19  to  our  consolidated  financial  statements  included
elsewhere in this Annual Report on Form 10-K for more information.

The  patent  positions  of  pharmaceutical  companies  can  be  highly  uncertain  and  involve  complex  legal  and  factual
questions  for  which  important  legal  principles  remain  unresolved.  No  consistent  policy  regarding  the  breadth  of  claims
allowed  in  pharmaceutical  patents  has  emerged  to  date  in  the  United  States  or  in  foreign  jurisdictions,  and  the  legal
standards relating to the patentability, validity and enforceability of pharmaceutical patents are evolving. Changes in either
the  patent  laws  or  in  interpretations  of  patent  laws  in  U.S.  and  foreign  jurisdictions  may  diminish  the  value  of  our
intellectual  property.  Accordingly,  we  cannot  predict  the  breadth  of  claims  that  may  be  enforced  in  the  patents  that  we
currently own or that may issue from the applications we have filed or may file in the future or those that we may license
from third parties. Additionally, our currently pending or future patent applications may not result in issued patents, and
any term extensions or reissues that we seek may not be granted. Further, if any patents we obtain or license are deemed
invalid or unenforceable, it could impact our ability to commercialize or license our technology or we may not be able to
prevent third parties from launching generic versions of our products, or from developing or marketing products that are
similar or identical to ours.

There have been numerous changes to the patent laws that may have a significant impact on our ability to protect our
technology and enforce our intellectual property rights. In September 2011, the America Invents Act was signed into law.
The  final  substantive  provisions  of  the  America  Invents  Act  became  effective  in  March  2013.  The  America  Invents  Act
included a number of significant changes to U.S. patent law that affect the way patent applications are filed, prosecuted and
litigated, including, among other things, changing from a “first to invent” to a “first inventor to file” system and creating
processes, such as Inter Partes Review (“IPR”) and other post-grant review processes, that permit third parties to challenge
the  validity  of  granted  patents  before  the  Patent  Trial  and  Appeal  Board  of  the  U.S.  Patent  and  Trademark  Office  (the
“USPTO”). The IPR process, for example, permits any person to challenge the validity of a patent on the grounds that it
was  anticipated  or  made  obvious  by  prior  art.  The  America  Invents  Act  and  its  implementation  could  increase  the
uncertainties and costs surrounding the prosecution of our patent applications and the enforcement or defense of our issued
patents,  all  of  which  could  have  a  material  adverse  effect  on  our  business,  financial  condition,  results  of  operations  and
growth prospects.

Others have filed, and in the future, are likely to file, patent applications covering products and technologies that are
similar or competitive to ours, or may be important to our business. We cannot be certain that any patent application owned
by a third party will not have priority over patent applications filed or in-licensed by us, or that we or our

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licensors will not be involved in infringement, interference, derivation, opposition, nullity, invalidity or other similar
proceedings before U.S. or non-U.S. patent offices or courts.

The degree to which our patents protect our products may be limited due to a number of factors. For example:

● others may be able to develop and market products that are similar to our products or product candidates but

not covered by the claims of our patents;

● we  might  not  have  been  the  first  to  conceive  of  the  inventions  covered  by  our  patents  or  pending  patent

applications;

● we might not have been the first to file patent applications for these inventions;

● patents that we obtain may not provide us with competitive advantages or exclusivity in a particular product

area or indication or for the length of time we have anticipated; or

● the patents of others may have an adverse effect on our business.

We are the owner of record of numerous issued U.S. and non-U.S. patents and patent applications with claims directed
to  pharmaceutical  compounds,  pharmaceutical  compositions,  formulations,  methods  of  making  these  compounds  and
methods of using these compounds in various indications.

Our issued patents for OCA are expected to expire between 2022 and 2036 if the appropriate maintenance, renewal,
annuity, or other government fees are paid. Without patent protection, including patent protection covering the composition
of  matter,  methods  of  using  and  formulations  of  our  products  and  product  candidates,  our  ability  to  stop  others  from
making, using, selling, offering to sell or importing our products and product candidates may be limited.

Due  to  the  patent  laws  of  a  specific  country  in  which  we  are  seeking  patent  protection,  the  decisions  of  a  patent
examiner in a specific country in which we are seeking patent protection or our own filing strategies, we ultimately may
not  obtain  patent  coverage  for  all  of  our  products  and  product  candidates  for  which  we  have  filed  a  patent  application.
While  we  regularly  pursue  patent  protection  in  the  United  States  and  other  countries  to  obtain  claim  coverage  for  our
inventions, we cannot be certain that such patent rights will be granted or that the scope of any patent granted will prevent
third parties from making, using, selling, offering for sale or importing the same or similar products.

If we do not obtain protection under the Hatch-Waxman Act in the United States (and similar legislation outside of the
United  States)  extending  the  terms  of  our  patents  and/or  providing  data  or  other  exclusivity  for  our  products  and
product candidates, our business may be materially harmed.

Depending upon the timing, duration and specifics of FDA marketing approval of our products, U.S. patents may be
eligible for a limited extension of patent term under the Drug Price Competition and Patent Term Restoration Act of 1984
(the “Hatch-Waxman Act”). The Hatch-Waxman Act permits an extension of patent term for one patent of up to five years
as compensation for patent term lost during product development and the FDA regulatory review process, so long as the
total period of patent term extension does not exceed 14 years from the date of approval. However, an extension may not
be  granted  because  of,  for  example,  failure  to  apply  within  applicable  deadlines,  failure  to  apply  prior  to  expiration  of
relevant  patents  or  failure  to  satisfy  applicable  requirements.  Moreover,  the  applicable  time  period  or  scope  of  patent
protection afforded could be less than what is requested. If we are unable to obtain patent term extension or the term of any
such  extension  is  less  than  what  we  request,  the  period  during  which  we  will  have  the  right  to  exclusively  market  our
products may be shorter than anticipated, our competitors may obtain approval of competing products following our patent
expiration and our revenue could be reduced, possibly materially.

In  October  2020,  the  USPTO  granted  to  the  Company  a  reissue  patent,  the  ‘286  Patent.  By  operation  of  law,  our
primary composition of matter patent protecting Ocaliva, the ‘390 Patent, was withdrawn and replaced by the ‘286 Patent,
which contains composition of matter claims to OCA. The ‘286 Patent has been substituted in any litigation where the

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‘390 Patent was asserted. The ‘286 Patent, like its predecessor the ‘390 Patent, was scheduled to expire in 2022. In light of
the  U.S.  marketing  approval  of  Ocaliva  for  PBC  in  May  2016,  and  pursuant  to  the  Hatch-Waxman  Act,  we  previously
applied for an extension of the patent term for the ‘390 Patent in the U.S. seeking to extend the term of the ‘390 Patent into
2027. After the ‘286 Patent was issued, the application for extension of patent term was transferred to the ‘286 Patent. In
February  2021,  a  patent  term  extension  certificate  was  issued,  which  extends  the  term  of  the  ‘286  Patent  into  2027.
Similarly,  in  connection  with  the  conditional  approval  of  Ocaliva  for  PBC  in  the  European  Union,  we  applied  for
supplementary protection certificates (“SPC”) to extend the patent term for the European analogue of the ‘390 Patent (now
the ‘286 Patent) in most of the European Union into 2027. To date, we have received grants of SPC in Austria, Belgium,
Cyprus, Denmark, Finland, France, Germany, Greece, Ireland, Italy, Luxembourg, Netherlands, Norway, Portugal, Spain,
Sweden,  Switzerland  and  the  United  Kingdom.  We  have  also  taken  similar  actions  in  other  jurisdictions  and  countries
where regulations providing for patent term extension exist. The issued patents for OCA are expected to expire between
2022 and 2036 if the appropriate maintenance, renewal, annuity, or other government fees are paid. The substitution in the
U.S. of the ‘286 Patent for the ‘390 Patent has no effect on foreign patent rights.

We  may  incur  substantial  costs  as  a  result  of  litigation  or  other  proceedings  relating  to  patent  and  other  intellectual
property rights, and such litigation may divert the attention of our management and scientific personnel and adversely
affect our development and commercialization efforts.

If we choose to file patent infringement lawsuits or engage in other adversarial proceedings to stop another party from
making,  using,  selling,  offering  for  sale  or  importing  the  inventions  claimed  in  any  of  our  patents,  that  individual  or
company alleged to be infringing has the right to ask the court or adjudicating body to rule that such patents are invalid, not
infringed or should not be enforced against that third party. These lawsuits and proceedings are expensive, consume time
and resources and divert the attention of management and scientific personnel even if we are successful in defending our
rights.  In  addition,  there  is  a  risk  that  such  court  or  adjudicating  body  will  decide  that  such  patents  are  invalid,
unenforceable  or  not  infringed,  and  that  we  do  not  have  the  right  to  stop  the  other  party  from  making,  using,  selling,
offering for sale or importing the inventions. For example, we have received paragraph IV certification notice letters from
six generic drug manufacturers indicating that each such company has submitted to the FDA an ANDA seeking approval to
manufacture and sell a generic version of our 5 mg and 10 mg dosage strengths of Ocaliva (obeticholic acid) for PBC prior
to  the  expiration  of  certain  patents  protecting  Ocaliva.  We  have  initiated  patent  infringement  suits  against  each  of  these
generic  drug  manufacturers  in  the  United  States  District  Court  for  the  District  of  Delaware.  Such  lawsuits  may  be
expensive and divert our management’s time and attention. In addition, to the extent such lawsuits are not successful, and a
generic equivalent of Ocaliva is approved and enters the market before the expiration of our patents protecting Ocaliva, our
business  may  be  materially  and  adversely  affected.  See  Note  19  to  our  consolidated  financial  statements  included
elsewhere in this Annual Report on Form 10-K for more information.

Over the past 20 years, the U.S. Supreme Court and the U.S. Congress have modified certain examination procedures
utilized  by  the  USPTO  in  granting  patents,  which  has  raised  the  standard  of  patentability  for  some  types  of  inventions.
Such modifications may reduce the likelihood that we will be able to obtain patent protection and increase the likelihood of
challenges to our patents or the patents we license.

We may infringe the intellectual property rights of others, which may prevent or delay our product development efforts
and/or delay, halt or increase the costs of our commercialization efforts.

Our success will depend in part on our ability to operate without infringing the proprietary rights of third parties. We
cannot guarantee that the use, manufacture, sale, offer for sale or importation of our products will not infringe third-party
patents.  Furthermore,  a  third  party  may  claim  that  we  or  our  manufacturing  or  commercialization  partners  are  using
inventions covered by the third party’s patent rights and may go to court to stop us from engaging in our normal operations
and  activities,  including  making  or  selling  our  products  and  product  candidates.  The  defense  of  these  lawsuits  is  often
costly and could affect our results of operations and divert the attention of our management and scientific personnel. There
is also a risk that a court could decide that we or our manufacturing or commercialization partners are infringing the third
party’s patents and order us or our partners to stop the activities covered by the patents. In that event, we or our partners
may  be  required  to  halt  or  delay  commercialization  or  development  of  the  relevant  product  or  product  candidate.  In
addition, there is a risk that a court could order us or our partners to pay the other party damages for having violated the
other party’s patents, and we may be subject to indemnification obligations with respect to any such payments made by

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our  partners.  There  is  a  vast  array  of  patents  and  patent  applications  that  claim  various  pharmaceutical  inventions  and
because the scope of a patent’s claims is subject to interpretation by the courts, it is not always clear to industry participants
which  patents  cover  various  types  of  products,  product  candidates  or  methods  of  use.  In  addition,  interpretation  of  a
patent’s claims can vary from court to court.

If we are sued for patent infringement, we would need to demonstrate that the relevant patent is not enforceable or that
our products, product candidates or methods either do not infringe the patent claims of the relevant patent or that the patent
claims are invalid. Proving invalidity, non-infringement and/or unenforceability is difficult, and we may not be successful.
For example, in the United States, proving invalidity requires a showing of clear and convincing evidence to overcome the
presumption of validity enjoyed by issued patents. Even if we are successful in such proceedings, we may incur substantial
costs and divert our management’s time and attention, which could have a material adverse effect on our business. If we are
unable to avoid infringing the patent rights of others, we may be required to seek a license, which may not be available,
defend  an  infringement  action  or  challenge  the  validity  of  the  patents  in  court.  Patent  litigation  is  costly  and  time
consuming. We may not have sufficient resources to bring these actions to a successful conclusion. In addition, if we fail to
obtain a license, develop or obtain non-infringing technology or defend an infringement action successfully, we may incur
substantial  monetary  damages,  encounter  significant  delays  in  the  commercialization  of  our  products  and  product
candidates and be precluded from manufacturing or selling our products and product candidates.

We cannot be certain that others have not filed patent applications for technology covered by our pending applications,

or that we were the first to invent or file with respect to a technology, because:

● some patent applications in the United States may be unpublished or otherwise maintained in secrecy until

the patents are issued;

● patent applications in the United States are typically not published until 18 months after the priority date; and

● publications in the scientific literature often lag behind actual discoveries.

Our competitors may have filed, and may in the future file, patent applications covering technology similar to ours.
Any such patent application may have priority over our patent applications, which could further require us to obtain rights
to issued patents covering such technologies. If another party has filed a U.S. patent application on inventions similar to
ours,  we  may  have  to  participate  in  an  interference,  derivation  or  other  similar  proceeding  declared  by  the  USPTO  to
determine priority of invention in the United States. The costs of these proceedings could be substantial, and it is possible
that  such  efforts  would  be  unsuccessful,  resulting  in  a  loss  of  our  U.S.  patent  position  with  respect  to  such  inventions.
Other countries have similar laws that permit secrecy of patent applications, and such patent applications may be entitled to
priority over our applications in such jurisdictions.

Some of our competitors may be able to sustain the costs of complex patent litigation more effectively than we can
because they have substantially greater financial and other resources. In addition, uncertainties resulting from the initiation
and continuation of any such litigation could have a material adverse effect on the market price of our securities and our
ability to raise the funds necessary to continue our operations.

Obtaining  and  maintaining  our  patent  protection  depends  on  compliance  with  various  procedural,  document
submission, fee payment and other requirements imposed by governmental patent agencies, and our patent protection
could be reduced or eliminated as a result of non-compliance with these requirements.

Periodic maintenance fees, renewal fees, annuity fees and various other governmental fees on our patents and patent
applications  are  required  to  be  paid  to  the  USPTO  and  foreign  patent  offices  in  several  stages  over  the  lifetime  of  such
patents and patent applications. In addition, the USPTO and foreign patent agencies require compliance with a number of
procedural,  documentary,  fee  payment  and  other  similar  provisions  during  the  patent  application  process.  We  have
implemented  systems  and  engaged  reputable  third-party  service  providers  to  help  ensure  that  we  comply  with  such
requirements  on  a  timely  basis,  but  inadvertent  lapses  may  occur  and  there  are  situations  in  which  noncompliance  can
result in abandonment or lapse of the relevant patent or patent application, resulting in partial or complete loss of patent

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rights in the relevant jurisdiction. Any such event may impair our competitive position in the relevant jurisdiction and have
a material adverse effect on our financial condition or results of operations.

We  may  be  subject  to  claims  that  our  employees  have  wrongfully  used  or  disclosed  alleged  trade  secrets  or  other
proprietary information of their former employers. In addition, if we are not able to adequately prevent disclosure of our
trade secrets and other proprietary information, the value of our technology, products and product candidates could be
significantly diminished.

As  is  common  in  the  biotechnology  and  pharmaceutical  industries,  we  employ  individuals  who  were  previously
employed  at  other  biotechnology  or  pharmaceutical  companies,  including  our  competitors  or  potential  competitors.  We
may be subject to claims that these employees, or we, have inadvertently or otherwise used or disclosed trade secrets or
other proprietary information of their former employers. Litigation may be necessary to defend against these claims, which
could result in substantial costs and be a distraction to our management even if we are successful.

We  may  rely  on  trade  secrets  to  protect  our  proprietary  technologies,  especially  where  we  do  not  believe  patent
protection  is  appropriate  or  obtainable.  However,  trade  secrets  are  difficult  to  protect,  and  may  not  prevent  others  from
independently and lawfully developing similar or identical products that circumvent our intellectual property. We rely in
part on confidentiality agreements with our employees, consultants, outside scientific collaborators, sponsored researchers
and  other  advisors  to  protect  our  trade  secrets  and  other  proprietary  information.  These  agreements  may  not  effectively
prevent  disclosure  of  proprietary  information  and  may  not  provide  an  adequate  remedy  in  the  event  of  unauthorized
disclosure of confidential information.

Third  parties,  including  competitors  of  ours,  may  also  independently  discover  our  trade  secrets  or  other  proprietary
information. In addition, we may be required under U.S. or foreign transparency initiatives or other regulations to publicly
disclose  or  otherwise  make  available  certain  information  that  we  consider  to  be  proprietary,  including  pre-clinical  and
clinical research data. Enforcing a claim that a third party illegally obtained and is using any of our trade secrets or other
proprietary information is expensive and time consuming, and the outcome is unpredictable. In addition, courts outside of
the United States are sometimes reluctant to protect trade secrets. Costly and time-consuming litigation could be necessary
to enforce and determine the scope of our proprietary rights, and failure to obtain or maintain protection of our trade secrets
and other proprietary information could adversely affect our competitive business position.

We  have  not  yet  registered  all  of  our  trademarks  and  failure  to  secure  such  registrations  could  adversely  affect  our
business.

We have numerous trademark and service mark registrations and pending trademark and service mark applications in

the United States and abroad.

Our trademark applications may not be allowed for registration and our registered trademarks may not be maintained
or enforced. During prosecution of applications for trademark registration, we may receive rejections or refusals. Although
we  are  given  an  opportunity  to  respond,  we  may  be  unable  to  overcome  such  rejections.  In  addition,  the  USPTO  and
comparable  agencies  in  many  other  jurisdictions  provide  third  parties  with  an  opportunity  to  oppose  pending  trademark
applications and to seek to cancel registered trademarks. Opposition or cancellation proceedings have been filed and may
in the future be filed against certain of our trademarks, and our trademarks may not survive such proceedings. If we do not
secure registrations for our trademarks, we may encounter more difficulty in enforcing them against third parties than we
otherwise would.

Trademark protection varies in accordance with local laws. Trademarks remain in force in some countries as long as
the trademark is used and in other countries as long as the trademark is registered. Trademark registrations generally are for
fixed but renewable terms. We cannot provide any assurances that any trademarks or service marks will be sufficient to
prevent competitors from adopting similar names. The adoption of similar names by competitors could impede our ability
to build brand identity and may lead to customer confusion, which could adversely affect our sales or profitability.

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Certain of our debt is secured and imposes covenants.

Risks Related to Our Indebtedness

In August 2021, we retired significant portions of our existing convertible notes by issuing $500.0 million in new 2026
Convertible  Secured  Notes.  These  new  notes  are  secured  by  a  first  priority  security  interest  in  substantially  all  assets  of
Intercept  Pharmaceuticals,  Inc.,  including  intellectual  property.  If  subsidiaries  of  Intercept  Pharmaceuticals,  Inc.  meet
certain threshold requirements, they may also become guarantors of the notes and subject to a requirement to pledge their
security interests.

The new notes also include additional covenants and other requirements compared with our other convertible notes,
including limits on incurrence of further indebtedness, limits on payment of dividends, limits on repayment of principal of
other indebtedness (other than repayment of the 2023 Convertible Notes at maturity, or before maturity at less than par),
limits  on  transfer  of  material  intellectual  property  to  subsidiaries  unless  the  subsidiaries  become  guarantors,  and
requirements  to  deliver  collateral  to  the  collateral  agent  and  enter  into  deposit  account  control  agreements  as  regards
certain of our bank accounts.

If we fail to comply with these requirements, fail to repay the debt, or otherwise default under these new notes, and the
indenture trustee and/or noteholders exercise remedies, they may foreclose on substantially all of our assets, and any such
default could also result in a default under our other outstanding indebtedness. Any of which would significantly impair
our business and the value of our stock.

We will need significant additional capital to retire or refinance our debt.

In August and September 2021, we refinanced and repurchased approximately 75% of our 2023 Convertible Notes.
We now have outstanding $113.7 million of 2023 Convertible Notes due July 1, 2023; $500.0 million 2026 Convertible
Secured Notes due February 15, 2026; and $115.3 million 2026 Convertible Notes due May 15, 2026.

Based on our current cash position, we will need to raise significant additional capital to repay our outstanding notes
maturing in 2026, either from operations, sale of assets, new debt, or new equity. We are not currently profitable, and sales
of significant assets could affect our business and future profitability. Given our level of indebtedness, new debt or new
equity financing to refinance or pay off our 2026 maturities may not be available on attractive terms, or at all, and, even if
available, the issuance of new equity or new convertible notes could dilute existing stockholders.

Our 2026 Convertible Secured Notes are secured by a first priority lien on substantially all assets, so we do not have
substantial  unsecured  assets  to  pledge  to  prospective  lenders.  The  2026  Convertible  Secured  Notes  impair  our  ability  to
incur debt maturing prior to their maturity. Lenders may be unwilling to lend on an unsecured basis beyond the maturity of
the  2026  Convertible  Secured  Notes.  If  we  do  retire  or  refinance  the  2023  Convertible  Notes  and  the  2026  Convertible
Secured Notes, we may still be limited in our ability to retire or refinance the 2026 Convertible Notes.

In  addition,  adverse  capital  market  conditions  may  significantly  affect  our  access  to  capital  and  ability  to  retire  or
refinance  our  debt.  Global  capital  markets  have  recently  experienced  significant  volatility,  and  obtaining  capital  may
become more difficult in the future due to such volatility or other market conditions, including rising interest rates, lower
stock  prices,  increased  risk  sensitivity  among  investors,  or  other  factors.  Thus,  we  may  not  be  able  to  access  capital
markets when needed, or on favorable terms.

Based on our Company's degree of financial leverage, failure to retire or refinance our debt could impair our ability to
invest in our business or engage in strategic transactions. Additionally, inability to repay our debts when due could trigger
collection efforts, noteholder remedies, and litigation, and significantly impair the value of our stock.

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The  issuance  of  shares  of  our  common  stock  upon  conversion  of  the  convertible  notes  would  dilute  the  ownership
interests of our stockholders and could depress the trading price of our common stock.

We may settle conversions of our outstanding convertible notes in cash, shares of our common stock or a combination
of cash and shares of our common stock. The issuance of shares of our common stock upon conversion of the convertible
notes would dilute the ownership interests of our stockholders, which could depress the trading price of our common stock.
In addition, the market’s expectation that conversions may occur could depress the trading price of our common stock even
in  the  absence  of  actual  conversions.  Moreover,  the  expectation  of  conversions  could  encourage  the  short  selling  of  our
common stock, which could place further downward pressure on the trading price of our common stock.

The accounting method for convertible debt securities that may be settled in cash, such as the Convertible Notes, could
have a material effect on our reported financial results.

Under Accounting Standards Codification Subtopic 470-20, “Debt with Conversion and Other Options” (“ASC 470-
20”), an entity must separately account for the liability and equity components of convertible debt instruments (such as the
Convertible Notes) that may be settled entirely or partially in cash upon conversion in a manner that reflects the issuer’s
economic interest cost. The effect of ASC 470-20 on the accounting for the Convertible Notes is that the equity component
is  required  to  be  included  in  the  additional  paid-in  capital  section  of  stockholders’  equity  on  our  consolidated  balance
sheets, and the value of the equity component is treated as original issue discount for purposes of accounting for the debt
component of the Convertible Notes. As a result, we are required to record a greater amount of non-cash interest expense in
current periods presented as a result of the amortization of the discounted carrying value of the Convertible Notes to their
face  amount  over  the  term  of  the  Convertible  Notes.  Because  ASC  470-20  requires  interest  to  include  both  the  current
period’s amortization of the debt discount and the instrument’s coupon interest, we report lower net income in our financial
results, which could adversely affect the market price of our common stock and the market price of the Convertible Notes.

In  addition,  under  certain  circumstances,  convertible  debt  instruments  (such  as  the  Convertible  Notes)  that  may  be
settled entirely or partly in cash are currently accounted for utilizing the treasury stock method, the effect of which is that
the shares issuable upon conversion of the Convertible Notes will not be included in the calculation of diluted earnings per
share except to the extent that the conversion value of the notes exceeds their principal amount. Under the treasury stock
method,  for  diluted  earnings  per  share  purposes,  the  transaction  is  accounted  for  as  if  the  number  of  shares  of  common
stock that would be necessary to settle such excess, if we elected to settle such excess in shares, are issued. We cannot be
sure  that  the  accounting  standards  in  the  future  will  continue  to  permit  the  use  of  the  treasury  stock  method.  If  we  are
unable to use the treasury stock method in accounting for the shares issuable upon conversion of the Convertible Notes,
then our diluted earnings per share would be adversely affected.

Risks Related to Ownership of Our Common Stock

Ownership in our common stock is highly concentrated and your ability to influence corporate matters may be limited
as a result.

Our executive officers, directors and stockholders who own more than 5% of our outstanding common stock together
beneficially own a significant percentage of our common stock based on reports filed with the SEC. If these stockholders
were  to  choose  to  act  together,  they  would  be  able  to  significantly  influence  matters  submitted  to  our  stockholders  for
approval, including the election of directors and approval of any merger, consolidation, sale of all or substantially all of our
assets or other business combination or reorganization, as well as our management and affairs. This concentration of voting
power  could  delay  or  prevent  an  acquisition  of  us  on  terms  that  other  securityholders  may  desire.  The  interests  of  this
group of stockholders may not always coincide with your interests or the interests of other securityholders and they may
act  in  a  manner  that  advances  their  best  interests  and  not  necessarily  those  of  other  securityholders,  including  seeking  a
premium value for their common stock, and might affect the market price of our common stock and the Convertible Notes.

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We have a significant stockholder, which will limit your ability to influence corporate matters, may give rise to conflicts
of interest and could result in future substantial sales of shares of our common stock into the market.

Genextra  S.p.A.  (“Genextra”)  is  one  of  our  largest  stockholders  and  owns  a  significant  minority  percentage  of  our
outstanding  common  stock.  Accordingly,  Genextra  exerts  and  will  continue  to  exert  influence  over  us  and  any  action
requiring  the  approval  of  the  holders  of  our  common  stock,  including  the  election  of  directors  and  amendments  to  our
organizational  documents,  such  as  increases  in  our  authorized  shares  of  common  stock  and  approval  of  significant
corporate transactions. This concentration of voting power makes it less likely that other holders of common stock will be
able to affect the way we are managed and could delay or prevent an acquisition of us on terms that other securityholders
may desire.

Furthermore,  the  interests  of  Genextra  may  not  always  coincide  with  the  interests  of  other  securityholders,  and
Genextra may act in a manner that advances its best interests and not necessarily those of other securityholders, including
seeking a premium value for its common stock, and might affect the market price of our common stock and the Convertible
Notes. Our board of directors, which consists of eleven directors, including one associated with Genextra, has the power to
set the number of directors on our board from time to time.

Genextra  also  may  sell  shares  of  our  common  stock  into  the  market  from  time  to  time,  and  we  cannot  predict  the

effect, if any, that future sales by Genextra may have on the market price of our common stock or the Convertible Notes.

An active trading market in our common stock may not be maintained.

The  trading  market  in  our  common  stock  has  been  extremely  volatile.  The  quotation  of  our  common  stock  on  the
Nasdaq Global Select Market does not assure that a meaningful, consistent and liquid trading market will exist. We cannot
predict whether an active market for our common stock will be maintained in the future. An absence of an active trading
market  could  adversely  affect  your  ability  to  sell  our  common  stock  at  current  market  prices  in  short  time  periods,  or
possibly at all. Additionally, market visibility for our common stock may be limited and such lack of visibility may have a
depressive effect on the market price for our common stock.

We have previously been, and are currently, subject to securities class action litigation and may be subject to similar or
other litigation in the future. Such matters can be expensive, time-consuming and have a material adverse effect on our
business, results of operations and financial condition.

We have previously been subject to securities class action lawsuits. In February 2014, two purported securities class
actions were filed against us and certain of our officers, which were eventually consolidated. In May 2016, the defendants
reached  an  agreement  with  the  lead  plaintiff  to  seek  court  approval  of  a  proposed  resolution  and  the  settlement  was
ultimately granted final approval by the court in September 2016. While the final judgment and order of the court included
a dismissal of the action with prejudice against all defendants and the defendants did not admit any liability as part of the
settlement, the total payment aggregated to $55.0 million, of which $10.0 million was paid by our insurers.

In September 2017, a lawsuit and, in January 2018, a follow-on lawsuit, were filed alleging that we and certain of our
officers  made  material  misrepresentations  and/or  omissions  of  material  fact  regarding  Ocaliva  dosing,  use  and
pharmacovigilance-related  matters,  as  well  as  our  operations,  financial  performance  and  prospects.  The  plaintiffs  seek
unspecified monetary damages on behalf of the putative class, an award of costs and expenses, including attorney’s fees,
and rescissory damages.

While  we  believe  that  we  have  a  number  of  valid  defenses  to  the  claims  described  above  and  intend  to  vigorously
defend ourselves, the matters are in the early stages of litigation and no assessment can be made as to the likely outcome of
the matters or whether they will be material to us.

Additionally, in November 2020, a lawsuit and, in December 2020 and February 2021, follow-on lawsuits, were filed
alleging that we and certain of our officers made material misrepresentations and/or omissions of material fact during the
period from September 28, 2019 to October 7, 2020 relating to our NDA for OCA for the treatment of liver fibrosis due to
NASH and the use of Ocaliva in patients with PBC, as well as our operations, financial performance and prospects. The

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plaintiff seeks unspecified monetary damages on behalf of the putative class, and an award of costs and expenses, including
attorney’s fees.

We  may  be  subject  to  additional  suits  or  proceedings  brought  in  the  future  and,  as  has  been  the  case  with  many
companies  in  our  industry,  we  may  from  time  to  time  receive  inquiries  and  subpoenas  and  other  types  of  information
requests  from  government  authorities  and  others.  While  the  ultimate  outcome  of  any  such  investigations,  inquiries,
information requests and legal proceedings is difficult to predict, adverse resolutions or settlements of those matters may
result in, among other things, modification of our business practices, product recalls, significant costs, payments, damages
or fines or other administrative, civil or criminal remedies, liabilities or penalties, which may have a material adverse effect
on our business, results of operations and financial condition. In addition, monitoring and defending against legal actions,
whether  or  not  meritorious,  and  responding  to  investigations,  inquiries  and  information  requests  is  expensive,  time-
consuming for our management and detracts from our ability to fully focus our internal resources on our business activities,
and  we  cannot  predict  how  long  it  may  take  to  resolve  such  matters.  Although  we  may  receive  insurance  coverage  for
certain adversarial proceedings, coverage could be denied or prove to be insufficient. It is possible that we could, in the
future, incur a judgment or enter into settlement of claims for monetary damages. A decision adverse to our interests could
result in the payment of substantial damages and could have a material adverse effect on our business, results of operations
and financial condition.

Our stock price has been and may in the future be volatile, which could cause holders of our common stock to incur
substantial losses.

The market price of our common stock has been, and is likely to continue to be, highly volatile and could be subject to
wide fluctuations in response to various factors, some of which are beyond our control. Since our initial public offering in
October 2012, the price of our common stock on the Nasdaq Global Select Market has ranged from $11.60 per share to
$497.00 per share. In addition to the other factors discussed in this “Risk Factors” section and elsewhere in this Annual
Report on Form 10-K, the factors that may result in wide fluctuations in the price of our common stock include any:

● delay, failure or receipt of regulatory approval for our product candidates, including OCA for liver fibrosis

due to NASH;

● delay,  failure  or  receipt  of  additional  marketing  authorizations  for  Ocaliva  or  our  product  candidates,

including OCA for liver fibrosis due to NASH, in our target markets;

● failure to successfully commercialize our approved products in the United States, the European Union and
our other target markets, or our inability to maintain regulatory approval for Ocaliva or our other approved
products in such markets;

● clinical  trial  failure,  including  any  such  failure  resulting  from  issues,  delays  or  difficulties  in  identifying
patients, enrolling patients, treating patients, retaining patients, meeting specific endpoints in the jurisdictions
in which we intend to seek approval or completing and timely reporting the results of our clinical trials, such
as our NASH and PBC trials;

● the effects of COVID-19 and related public health safety measures and business closures and disruptions;

● inability to obtain additional funding;

● delay in filing an investigational new drug application, NDA, MAA or comparable submission for any of our
product  candidates,  and  any  adverse  development  or  perceived  adverse  development  with  respect  to  the
regulatory review of any such submission;

● potential  side  effects  associated  with  Ocaliva  for  PBC,  OCA  for  liver  fibrosis  due  to  NASH  or  our  other

product candidates;

● inability to obtain adequate product supply of Ocaliva, OCA for liver fibrosis due to NASH or any of our

other product candidates or the inability to do so at acceptable prices;

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● results of clinical trials of our competitors’ products and product candidates;

● regulatory  or  advisory  committee  actions  or  recommendations  with  respect  to  our  products  or  product
candidates,  including  Ocaliva  or  OCA  for  liver  fibrosis  due  to  NASH,  or  our  competitors’  products  or
product candidates;

● changes in laws or regulations applicable to our products or product candidates;

● failure to meet or exceed financial projections or guidance we may provide to the public;

● failure to meet or exceed the estimates and projections of the investment community;

● actual or anticipated fluctuations in our financial condition and operating results;

● actual or anticipated changes in our growth rate relative to our competitors;

● actual or anticipated fluctuations in our competitors’ operating results or changes in their growth rate;

● competition from existing products or new products that may emerge;

● announcements  by  us,  our  collaborators  or  our  competitors  of  significant  acquisitions,  strategic

collaborations, joint ventures, collaborations or capital commitments;

● issuance of new or updated research or reports by securities analysts;

● fluctuations in the valuation of companies perceived by investors to be comparable to us;

● share price and volume fluctuations attributable to inconsistent trading volume levels of our shares;

● additions or departures of key management or scientific personnel;

● disputes  or  other  developments  related  to  proprietary  rights,  including  patents,  litigation  matters  and  our

ability to obtain patent protection for our technologies;

● announcement or expectation of additional financing efforts;

● disputes,  governmental  inquiries  or  investigations,  legal  proceedings  or  litigation,  including  any  securities,

intellectual property, employment, product liability or other litigation;

● sales of our common stock by us, our insiders or our other stockholders;

● failure  to  adopt  appropriate  information  security  systems,  including  any  systems  that  may  be  required  to
prevent  or  defend  against  system  failures  or  security  or  security  or  data  breaches  due  to  cyber-attacks,  or
cyber intrusions, including ransomware, phishing attacks and other malicious intrusions;

● failure to comply with data protection laws;

● market conditions for biopharmaceutical stocks in general; and

● general economic, industry, market and political conditions.

Any of these factors could also affect the trading price of the Convertible Notes.

Furthermore,  stock  markets  in  general  and  the  market  for  biotechnology  companies  in  particular  have  experienced
extreme  price  and  volume  fluctuations  that  have  affected  and  continue  to  affect  the  market  prices  of  securities  of  many
companies.  These  fluctuations  often  have  been  unrelated  or  disproportionate  to  the  operating  performance  of  those
companies. A number of factors, including global health catastrophes (e.g., COVID-19), general economic, political and
market conditions, recessions, interest rate changes or international currency fluctuations may negatively impact the

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market price of our securities, regardless of our actual operating performance. In the past, companies that have experienced
volatility in the market price of their stock have been subject to securities class action litigation. We have been in the past,
and  are  currently  subject  to  this  type  of  litigation,  which  could  result  in  substantial  costs  and  divert  our  management’s
attention from other business concerns, which could seriously harm our business. As a result of this volatility, you could
incur substantial losses.

If  our  stockholders  sell  substantial  amounts  of  our  common  stock,  the  market  price  of  our  common  stock  or  the
Convertible Notes may decline even if our business is doing well.

A significant number of shares of our common stock are held by a small number of stockholders, including Genextra.
Sales  of  a  significant  number  of  shares  of  our  common  stock,  or  the  expectation  that  such  sales  may  occur,  could
significantly  reduce  the  market  price  of  our  common  stock  or  the  Convertible  Notes.  These  sales,  or  the  possibility  that
these sales may occur, also might make it more difficult for us to sell equity securities in the future at a time and price that
we deem appropriate. We have also registered the offer and sale of the shares of common stock that we may issue under
our equity compensation plans, including upon the exercise of stock options. These shares may be freely sold in the public
market upon issuance.

Additionally, sales of our common stock by our executive officers or directors, even when done during an open trading
window  under  our  policies  with  respect  to  insider  sales  or  done  under  a  trading  plan  adopted  in  accordance  with  the
guidelines set forth by Rule 10b5-1, may adversely impact the market price of our common stock or the Convertible Notes.
Although we do not expect that the relatively small volume of such sales would itself significantly impact the market price
of our common stock or the Convertible Notes, the market could react negatively to the announcement of such sales, which
could in turn affect the market price of our common stock and the Convertible Notes.

You may experience future dilution as a result of future equity offerings or strategic transactions.

We  may  in  the  future  raise  funds  through  the  issuance  and  sale  of  additional  shares  of  our  common  stock  or  other
securities convertible into or exchangeable for our common stock. For example, in August 2021, we issued $500.0 million
aggregate  principal  amount  of  the  2026  Convertible  Secured  Notes,  in  May  2019,  we  issued  and  sold  an  aggregate  of
2,879,760  shares  of  common  stock  and  $230.0  million  aggregate  principal  amount  of  the  2026  Convertible  Notes,  in
April 2018, we issued and sold an aggregate of 4,257,813 shares of common stock and in July 2016, we issued and sold
$460.0 million aggregate principal amount of the 2023 Convertible Notes. Conversions of the Convertible Notes will dilute
the  ownership  interests  of  existing  shareholders  to  the  extent  that  we  elect  to  deliver  shares  of  our  common  stock  (or  a
combination of cash and shares of our common stock) in connection therewith. In addition, the existence of the Convertible
Notes may encourage short selling by market participants because the conversion of the Convertible Notes could depress
the price of our common stock. We may also issue shares of common stock, stock options, restricted stock, restricted stock
units  or  other  stock-based  awards  under  our  existing  or  future  equity  incentive  plans  or  other  employee  or  director
compensation  plans.  The  issuance  of  additional  shares  of  common  stock  (including  pursuant  to  conversions  of  the
Convertible Notes) or other securities convertible into or exchangeable for our common stock, or the perception that such
issuances may occur, may materially and adversely affect the price of our common stock and the Convertible Notes.

Anti-takeover  provisions  in  our  restated  certificate  of  incorporation  and  our  restated  bylaws,  as  well  as  provisions  of
Delaware law and certain provisions of the Convertible Notes, might discourage, delay or prevent a change in control of
our  company  or  changes  in  our  management  and,  therefore,  depress  the  market  price  of  our  common  stock  or  the
Convertible Notes.

Provisions in our restated certificate of incorporation and restated bylaws, as well as provisions of Delaware law, may
discourage, delay or prevent a merger, acquisition or other change in control that our securityholders consider favorable,
including transactions in which securityholders might otherwise receive a premium for their securities. These provisions
may  also  prevent  or  frustrate  attempts  by  our  stockholders  to  replace  or  remove  our  management.  Our  corporate
governance documents include provisions:

● authorizing the issuance of “blank check” convertible preferred stock, the terms of which may be established

and shares of which may be issued without stockholder approval;

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● prohibiting stockholder action by written consent, thereby requiring all stockholder actions to be taken at a
meeting  of  our  stockholders,  to  the  extent  that  no  stockholder,  together  with  its  affiliates,  holds  more  than
50% of our voting stock;

● eliminating the ability of stockholders to call a special meeting of stockholders;

● permitting  our  board  of  directors  to  accelerate  the  vesting  of  outstanding  equity  awards  upon  certain

transactions that result in a change of control; and

● establishing  advance  notice  requirements  for  nominations  for  election  to  the  board  of  directors  or  for

proposing matters that can be acted upon at stockholder meetings.

In  addition,  as  a  Delaware  corporation,  we  are  subject  to  provisions  of  Delaware  law,  including  Section  203  of  the
Delaware  General  Corporation  Law  (the  “DGCL”),  which  prevents  some  stockholders  holding  more  than  15%  of  our
outstanding common stock from engaging in certain business combinations without approval of the holders of substantially
all  of  our  outstanding  common  stock.  Any  provision  of  our  restated  certificate  of  incorporation  or  restated  bylaws  or
Delaware  law  that  has  the  effect  of  delaying  or  deterring  a  change  in  control  could  limit  the  opportunity  for  our
securityholders to receive a premium for their securities, and could also affect the price that some investors are willing to
pay for our common stock or the Convertible Notes.

Certain provisions of the Convertible Notes could also make it more difficult or more expensive for a third party to
acquire  us.  For  example,  if  an  acquisition  event  constitutes  a  “fundamental  change”  under  the  terms  of  the  Convertible
Notes,  holders  of  the  Convertible  Notes  will  have  the  right  to  require  us  to  purchase  their  Convertible  Notes  for  cash.
Similarly, if an acquisition event constitutes a “make-whole fundamental change” under the terms of the Convertible Notes,
we  may  be  required  to  increase  the  conversion  rate  for  holders  who  convert  their  Convertible  Notes  in  connection  with
such make-whole fundamental change.

The existence of the foregoing provisions and anti-takeover measures may also frustrate or prevent any attempts by
our stockholders to replace or remove our current management or members of our board of directors and could limit the
price that investors might be willing to pay in the future for shares of our common stock or the Convertible Notes. They
could also deter potential acquirers of our company, thereby reducing the likelihood that our securityholders could receive
a premium for their securities in an acquisition.

Claims  for  indemnification  by  our  directors  and  officers  may  reduce  our  available  funds  to  satisfy  successful
stockholder claims against us and may reduce the amount of money available to us.

As  permitted  by  Section  102(b)(7)  of  the  DGCL,  our  restated  certificate  of  incorporation  limits  the  liability  of  our
directors  to  the  fullest  extent  permitted  by  law.  In  addition,  as  permitted  by  Section  145  of  the  DGCL,  our  restated
certificate  of  incorporation  and  restated  bylaws  provide  that  we  shall  indemnify,  to  the  fullest  extent  authorized  by  the
DGCL,  each  person  who  is  involved  in  any  litigation  or  other  proceeding  because  such  person  is  or  was  a  director  or
officer of our company, or is or was serving as an officer or director of another entity at our request, against all expense,
loss or liability reasonably incurred or suffered in connection therewith. Our restated certificate of incorporation provides
that the right to indemnification includes the right to be paid expenses incurred in defending any proceeding in advance of
its final disposition, subject to certain conditions. The rights conferred in the restated certificate of incorporation and the
restated  bylaws  are  not  exclusive,  and  we  are  authorized  to  enter  into  indemnification  agreements  with  our  directors,
officers, employees and agents and to obtain insurance to indemnify such persons.

The above limitations on liability and our indemnification obligations limit the personal liability of our directors and
officers for monetary damages for breach of their fiduciary duty by shifting the burden of such losses and expenses to us.
Although we carry directors’ and officers’ liability insurance, certain liabilities or expenses covered by our indemnification
obligations may not be covered by such insurance or the coverage limitation amounts may be exceeded. As a result, we
may need to use a significant amount of our funds to satisfy our indemnification obligations, which could severely harm
our  business  and  financial  condition  and  limit  the  funds  available  to  securityholders  who  may  choose  to  bring  a  claim
against our company.

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We do not intend to pay dividends in the foreseeable future.

We do not anticipate paying cash dividends in the future. As a result, only appreciation of the price of shares of our
common  stock  will  provide  a  return  to  stockholders,  which  may  not  occur.  Investors  seeking  cash  dividends  should  not
invest in our common stock. You may not realize any return on your investment in our common stock and may lose some
or all of your investment.

Our ability to use our net operating loss carryforwards and certain other tax attributes may be limited.

We  have  significant  net  operating  loss  carryforwards  (“NOLs”)  for  U.S.  Federal,  state  and  foreign  income  tax
purposes. The enactment of the Tax Cuts and Jobs Act enacted in 2017 (the “TCJA”) modified the ability of companies to
utilize U.S. Federal NOLs arising in tax years beginning on or after January 1, 2018, by providing that such NOLs may be
carried-forward indefinitely and used to offset up to 80 percent of taxable income in any given future year. Existing NOLs
that arose in tax years beginning prior to January 1, 2018, were not affected by the TCJA and are generally eligible to be
carried-forward  for  up  to  20  years  and  used  to  fully  offset  taxable  income  in  future  years.  If  not  utilized,  our  pre-2018
NOLs will expire for U.S. Federal income tax purposes between 2024 and 2037. In addition, the Biden administration is
proposing  changes  to  the  Internal  Revenue  Code.  It  is  not  yet  clear  what  effect  such  tax  legislation  would  have  on  our
NOLs,  financial  condition,  and  results  of  operations.  We  also  have  certain  state  and  foreign  NOLs  in  varying  amounts
depending on the different state and foreign tax laws.

In  addition,  our  ability  to  utilize  our  NOLs  may  be  limited  under  Section  382  of  the  Internal  Revenue  Code  or
applicable  state  and  foreign  tax  law.  The  Section  382  limitations  apply  if  an  “ownership  change”  occurs.  Generally,  an
ownership change occurs when certain shareholders increase their aggregate ownership by more than 50 percentage points
over their lowest ownership percentage in a testing period (typically three years). We have evaluated whether one or more
ownership changes under Section 382 have occurred since our inception and have determined that there have been at least
two  such  changes.  Although  we  believe  that  these  ownership  changes  have  not  resulted  in  material  limitations  on  our
ability to use these NOLs, our ability to utilize these NOLs may be limited due to future ownership changes or for other
reasons.  As  a  result,  we  may  not  be  able  to  take  full  advantage  of  our  NOL  carryforwards  for  U.S.  Federal,  state,  and
foreign income tax purposes.

General Risk Factors

We may use our limited financial and human resources to pursue a particular research program or product candidate
that is ultimately unsuccessful or less successful than other programs or product candidates that we may have forgone
or delayed.

Because  we  have  limited  resources,  we  may  forego  or  delay  the  development  of  certain  programs  or  product
candidates that later prove to have greater commercial potential than the programs or product candidates that we do pursue.
Our  resource  allocation  decisions  may  cause  us  to  fail  to  capitalize  on  viable  commercial  products  or  profitable  market
opportunities.  Our  spending  on  current  and  future  research  and  development  programs  for  product  candidates  may  not
yield any commercially viable products. If we fail to accurately evaluate the commercial potential or target market for a
particular product candidate, we may relinquish valuable rights to that product candidate through strategic collaboration,
licensing or other arrangements or we may allocate our limited internal resources to that product candidate when it would
have been more advantageous to enter into such an arrangement. Any such failure could have a material adverse effect on
our business, financial condition or results of operations.

If we engage in a licensing transaction, acquisition, reorganization or business combination, we will face a variety of
risks that could adversely affect our business operations and our securityholders.

From time to time, we have considered, and we will continue to consider in the future, strategic business initiatives

intended to further the expansion and development of our business. These initiatives may include in-licensing or acquiring

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products, technologies or businesses, entering into a business combination with another company or otherwise partnering
with another company. If we pursue such a strategy, we could, among other things:

● issue equity securities that would dilute our current stockholders’ ownership;

● incur substantial debt that may place strains on our operations;

● be  required  to  dedicate  substantial  operational,  financial  and  management  resources  to  integrate  new

products, technologies or businesses;

● assume substantial actual or contingent liabilities;

● impair  our  ability  to  make  payments  of  interest  and  principal  on  our  outstanding  debt,  including  the

Convertible Notes;

● reprioritize our development programs or cease development and commercialization activities with respect to

certain of our product candidates or approved products; or

● merge  or  otherwise  enter  into  a  business  combination  with  another  company,  which  may  result  in  our
stockholders receiving cash and/or securities of the other company on terms that certain of our stockholders
may not deem desirable.

Our  insurance  policies  are  expensive  and  only  protect  us  from  some  business  risks,  which  leave  us  exposed  to
significant uninsured liabilities.

We do not carry insurance for all categories of risk that our business may encounter. Some of the policies we currently
maintain  include  general  liability,  employment  practices  liability,  property,  auto,  workers’  compensation,  cyber  liability,
products liability and directors’ and officers’ insurance. We do not know, however, if our current levels of coverage are
adequate or if we will be able to obtain insurance with adequate levels of coverage in the future, if at all. Any significant
uninsured  liability,  including  significant  uninsured  liabilities  resulting  from  COVID-19  or  related  public  health  safety
measures  or  business  closures  and  disruptions,  may  require  us  to  pay  substantial  amounts,  which  could  materially  and
adversely  affect  our  financial  position  and  results  of  operations.  Furthermore,  any  increase  in  the  volatility  of  our  stock
price,  among  other  factors,  may  result  in  us  being  required  to  pay  substantially  higher  premiums  for  our  directors’  and
officers’ insurance, and may make it difficult for us to obtain adequate coverage on reasonable terms, if at all.

We must comply with environmental, health and safety laws and regulations

Our activities involve the controlled storage, use and disposal of hazardous materials. We are subject to federal, state,
city and local laws and regulations, in and outside the United States, governing the use, manufacture, storage, handling and
disposal of these hazardous materials. Although we believe that the safety procedures we use for handling and disposing of
these materials comply with the standards prescribed by applicable laws and regulations, we cannot eliminate the risk of
accidental contamination or injury from these materials. In the event of an accident, regulatory authorities may curtail the
use of these materials and interrupt our business operations. We do not currently maintain hazardous materials insurance
coverage.

Failure to establish and maintain adequate financial infrastructure and accounting systems and controls could impair
our ability to comply with the financial reporting and internal controls requirements for publicly traded companies.

As  a  public  company,  we  operate  in  a  demanding  regulatory  environment,  which  requires  us  to  comply  with  the
Sarbanes-Oxley  Act  of  2002  and  related  rules  and  regulations,  expanded  disclosure  requirements,  accelerated  reporting
requirements and complex accounting rules. Responsibilities imposed by the Sarbanes-Oxley Act include establishing and
maintaining corporate oversight and adequate internal control over financial reporting and disclosure controls and

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procedures. Effective internal controls are necessary for us to produce reliable financial reports and are important to help
prevent financial fraud.

In particular, our compliance with Section 404 of the Sarbanes-Oxley Act has required and will continue to require that
we incur substantial accounting-related expenses and expend significant management efforts. Our testing, or the testing by
our  independent  registered  public  accounting  firm,  may  reveal  deficiencies  in  our  internal  controls  that  we  would  be
required to remediate in a timely manner. If we are not able to comply with the requirements of the Sarbanes-Oxley Act,
we  could  be  subject  to  sanctions  or  investigations  by  the  SEC,  the  Nasdaq  Global  Select  Market  or  other  regulatory
authorities,  which  would  require  additional  financial  and  management  resources  and  could  adversely  affect  the  market
price of our securities. Furthermore, if we cannot provide reliable financial reports or prevent fraud, including as a result of
remote working by our employees in connection with COVID-19 and related public health safety measures, our business
and results of operations would likely be materially and adversely affected.

Our disclosure controls and procedures may not prevent or detect all errors or acts of fraud.

We are subject to the periodic reporting requirements of the Exchange Act. Our disclosure controls and procedures are
designed  to  reasonably  assure  that  information  required  to  be  disclosed  by  us  in  reports  we  file  or  submit  under  the
Exchange Act is accumulated and communicated to management, recorded, processed, summarized and reported within the
time periods specified in the rules and forms of the SEC. We believe that any disclosure controls and procedures or internal
controls and procedures, no matter how well conceived and operated, can provide only reasonable, not absolute, assurance
that the objectives of the control system are met.

These inherent limitations include the realities that judgments in decision-making can be faulty and that breakdowns
can occur because of simple error or mistake. Additionally, controls can be circumvented by the individual acts of some
persons, by collusion of two or more people or by an unauthorized override of the controls. Accordingly, because of the
inherent limitations in our control system, misstatements or insufficient disclosure due to error or fraud may occur and not
be detected.

Changes in our effective income tax rate could adversely affect our results of operations.

We  are  subject  to  income  taxes  in  the  United  States  and  various  foreign  jurisdictions.  Various  factors  may  have
favorable  or  unfavorable  effects  on  our  effective  income  tax  rate.  These  factors  include,  but  are  not  limited  to,
interpretations of existing tax laws, changes in tax laws and rates, such as the TCJA, the accounting for stock options and
other  stock-based  compensation,  changes  in  accounting  standards,  future  levels  of  research  and  development  spending,
changes in the mix and level of pre-tax earnings in different jurisdictions, the outcome of audits or other examinations by
the U.S. Internal Revenue Service and tax regulators in other jurisdictions, the accuracy of our estimates for unrecognized
tax  benefits,  the  realization  of  deferred  tax  assets  and  changes  to  our  ownership  or  capital  structure.  The  Biden
administration  is  proposing  changes  to  the  Internal  Revenue  Code  that  could  include  material  increases  to  corporate  tax
rates. It is not yet clear what effect such tax legislation would have on our financial condition and results of operations.

The impact on our effective income tax rate resulting from these factors may be significant and could adversely affect

our results of operations.

If securities or industry analysts cease publishing research or reports about us, our business or our market, or if they
publish inaccurate or unfavorable reports about us or our securities, the price of our securities and trading volume in
our securities could decline.

The market for our common stock and the Convertible Notes depends in part on the research and reports that securities
or  industry  analysts  publish  about  our  company.  We  do  not  have  any  control  over  these  analysts,  and  there  can  be  no
assurance that analysts will continue to cover us or provide favorable coverage. If one or more of the analysts who cover us
downgrade  our  common  stock  or  publish  inaccurate  or  unfavorable  research  about  our  business,  our  stock  price  and  the
price of the Convertible Notes may decline. If one or more of the analysts covering us fail to regularly publish reports on
us, demand for our common stock and the Convertible Notes may decline, which could cause our stock price and the price
of the Convertible Notes and trading volume to decline.

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Item 1B.  Unresolved Staff Comments

None.

Item 2.   Properties

Our corporate headquarters are located at 10 Hudson Yards in New York, New York, where we lease and occupy an
aggregate of approximately 45,600 square feet of office space. The lease covering this property is scheduled to expire in
March  2022.  Our  corporate  headquarters  will  move  to  Morristown,  New  Jersey,  where  we  will  lease  and  occupy
approximately 26,000 square feet of office space under a separate lease that is expected to commence around March 2022
and scheduled to expire approximately 5.5 years from the commencement date.

Our research and development operations are based in San Diego, California, where we lease and occupy an aggregate
of approximately 34,000 square feet of space. The lease covering this property is currently scheduled to expire in October
2025.

We also lease and occupy approximately 8,600 square feet of office space in London, United Kingdom, which serves
as  the  headquarters  for  our  international  operations.  The  lease  covering  this  property  is  currently  scheduled  to  expire  in
May 2024.

We believe that our existing facilities are adequate for our immediate needs and that, should it be needed, additional

space can be leased to accommodate any future growth.

Item 3.   Legal Proceedings

For  a  description  of  our  significant  legal  proceedings,  see  Note  19  to  our  audited  consolidated  financial  statements

included elsewhere in this Annual Report on Form 10-K and incorporated by reference herein.

Item 4.   Mine Safety Disclosures

Not applicable.

PART II

Item 5.   Market for Registrant’s Common Equity, Related Stockholder Matters and Issuer Purchases of Equity
Securities

Market Information and Stockholders

Our common stock trades on the Nasdaq Global Select Market under the symbol “ICPT”. As of December 31, 2021,
there were 29,572,953 shares of our common stock issued and outstanding and approximately 100 stockholders of record.
A  significantly  larger  number  of  stockholders  may  hold  their  shares  in  “street  name”  through  banks,  brokers  and  other
nominees. The number of stockholders of record does not include stockholders who hold their shares in “street name.”

Stock Price Performance Graph

The following graph compares the cumulative total stockholder return for our common stock to the cumulative total
stockholder return for the Nasdaq Composite Index and the Nasdaq Biotechnology Index, in each case, for the period from
December 31, 2016 through December 31, 2021. The graph assumes an initial investment of $100 in our common stock at
the closing price of $108.65 on December 31, 2016 and in the Nasdaq Composite Index and the Nasdaq Biotechnology
Index on December 31, 2016 and the reinvestment of dividends. The stock performance shown below is not intended to
forecast  or  be  indicative  of  the  possible  future  performance  of  our  common  stock,  and  we  do  not  make  or  endorse  any
predications  as  to  future  stockholder  returns.  The  following  stock  performance  information  shall  not  be  deemed  to  be
“soliciting material,” “filed” with the U.S. Securities and Exchange Commission (the “SEC”), incorporated by reference

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into any filing under the Securities Act of 1933, as amended (the “Securities Act”), or the Securities Exchange Act of 1934,
as amended (the “Exchange Act”), or subject to the liabilities of Section 18 of the Exchange Act, except to the extent that
we specifically incorporate it by reference into a document filed under the Securities Act or the Exchange Act.

Among Intercept Pharmaceuticals, Inc., the Nasdaq Composite Index and

Comparison of Cumulative Total Return

the Nasdaq Biotechnology Index

$100 investment in stock or index
Intercept Pharmaceuticals, Inc.
Nasdaq Composite Index
Nasdaq Biotechnology Index

Dividend Policy

2016

2017

December 31,

2018

2019

2020

2021

$ 100.00
$ 100.00
$ 100.00

$  53.77
$ 129.64
$ 121.63

$  92.77
$ 125.96
$ 110.85

$ 114.05
$ 172.18
$ 138.69

$  22.73
$ 249.51
$ 175.33

$  14.99
$  304.85
$  175.37

We have never declared or paid any cash dividends on our common stock, and we do not anticipate paying any cash
dividends  in  the  foreseeable  future.  The  first  supplemental  indenture  for  the  recently  issued  2026  Convertible  Secured
Notes restricts the Company from declaring or paying cash dividends.

Recent Sales of Unregistered Securities

On  August  17,  2021,  the  Company  sold  $500.0  million  of  2026  Convertible  Secured  Notes  in  exchange  for  old
convertible notes and in a new subscription for cash, as described below in “Long-Term Debt” in the notes to our financial
statements. These new notes were issued in a private placement to institutional investors in reliance on the exemption from
registration provided by Section 4(a)(2) of the Securities Act.

As of August 20, 2021, the Company agreed with its financial advisor in the exchange and issuance, J. Wood Capital
Advisors  LLC,  to  settle  its  financial  advisory  fee  for  services  rendered  through  issuance  of  769,823  shares  of  common
stock,  equivalent  to  $10.0  million.  These  shares  were  issued  in  a  private  placement  in  reliance  on  the  exemption  from
registration provided by Section 4(a)(2) of the Securities Act.

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Of  the  new  2026  Convertible  Secured  Notes,  $117.6  million  were  issued  at  par  for  cash.  Substantially  all  proceeds

were used either for the repurchase of 4,521,502 shares of common stock in connection with the notes issuance for $75.8
million, or the repurchase in September 2021 of additional 2023 Convertible Notes for $38.1 million.

The  2026  Convertible  Secured  Notes  are  convertible  into  shares  of  common  stock,  with  the  terms  of  conversion
described  under  “Long-Term  Debt”,  which  have  not  been  registered  under  the  Securities  Act.  The  2026  Convertible
Secured Notes contain various covenants, including limitations upon the payment of dividends.

Issuer Purchases of Equity Securities

We did not purchase any of our registered equity securities during the three months ended December 31, 2021.

Item 6. [Reserved]

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Item 7.   Management’s Discussion and Analysis of Financial Condition and Results of Operations

You should read the following discussion and analysis together with our audited consolidated financial statements and
accompanying  notes  included  elsewhere  in  this  Annual  Report  on  Form  10-K.  This  discussion  and  analysis  contains
forward-looking  statements,  which  involve  risks  and  uncertainties.  As  a  result  of  many  factors,  such  as  those  described
under “Cautionary Note Regarding Forward-Looking Statements,” “Risk Factors,” and elsewhere in this Annual Report
on Form 10-K, our actual results may differ materially from those anticipated in these forward-looking statements.

Overview

We are a biopharmaceutical company focused on the development and commercialization of novel therapeutics to treat
progressive non-viral liver diseases with high unmet medical need utilizing our proprietary bile acid chemistry. Our first
marketed  product,  Ocaliva®  (obeticholic  acid  or  “OCA”),  is  a  farnesoid  X  receptor  (“FXR”)  agonist  approved  in  the
United States, the United Kingdom, the European Union and several other jurisdictions for the treatment of primary biliary
cholangitis (“PBC”) in combination with ursodeoxycholic acid (“UDCA”) in adults with an inadequate response to UDCA
or as monotherapy in adults unable to tolerate UDCA.

In addition to commercializing OCA for PBC under the Ocaliva brand name, we are also currently developing OCA
for additional indications, including nonalcoholic steatohepatitis (“NASH”). We are also developing product candidates in
various  stages  of  clinical  and  preclinical  development.  We  believe  that  OCA  and  our  other  product  candidates  have  the
potential  to  treat  orphan  and  other  more  prevalent  liver  diseases  such  as  NASH  for  which  there  are  currently  limited
therapeutic options.

Ocaliva  was  approved  for  PBC  by  the  U.S.  Food  and  Drug  Administration  (“FDA”)  in  May  2016  under  the
accelerated approval pathway. We commenced sales and marketing of Ocaliva in the United States shortly after receiving
approval,  and  Ocaliva  is  now  available  to  U.S.  patients  primarily  through  a  network  of  specialty  pharmacy  distributors.
Ocaliva received conditional approval for PBC from the European Commission in December 2016 and we commenced our
commercial launches across Europe (including the United Kingdom) in January 2017. In addition, we continue to work to
execute on our post-marketing regulatory commitments with respect to Ocaliva in the U.S. and Europe. We will continue to
generate  placebo  controlled  data  from  the  COBALT  trial  as  well  as  data  from  studies  utilizing  real  world  evidence  in
support of a broader evidence data package, which we anticipate submitting to the FDA and the EMA in the second half of
2022. If this data package does not support fulfillment of our post-marketing obligations, we may not be able to maintain
our previously granted marketing approvals of Ocaliva for PBC.

Our  lead  development  product  candidate  is  OCA  for  the  potential  treatment  of  NASH.  In  February  2019,  we
announced  topline  results  from  the  planned  18-month  interim  analysis  of  our  pivotal  Phase  3  clinical  trial  of  OCA  in
patients with liver fibrosis due to NASH, known as the REGENERATE trial. The REGENERATE trial is ongoing and is
expected  to  continue  through  clinical  outcomes  for  verification  and  description  of  the  clinical  benefit  of  OCA.  In  June
2020, we received a complete response letter (“CRL”) from the FDA stating that our NDA for OCA for the treatment of
liver fibrosis due to NASH could not be approved in its present form. We had our end of review meeting with the FDA in
October 2020 to discuss the FDA’s risk-benefit assessment in the CRL based on its review of the available data, as well as
our proposed resubmission of our NDA for the treatment of liver fibrosis due to NASH. The meeting was constructive and
the  FDA  provided  us  with  helpful  guidance  regarding  supplemental  data  we  can  provide  to  further  characterize  OCA’s
efficacy and safety profile that could support resubmission based on our Phase 3 REGENERATE 18-month biopsy data,
together with a safety assessment from our ongoing studies.

Following our end of review meeting, we have held a productive dialogue with FDA regarding  the  REGENERATE
study to clarify data, a new consensus read methodology for liver biopsies, and analyses required to resubmit our NDA. We
are  also  in  the  process  of  generating  a  new  data  package  from  our  REGENERATE  study  using  the  new  liver  biopsy
consensus  read  methodology,  and  if  the  data  supports  accelerated  approval,  we  plan  to  have  a  potential  pre-NDA
submission meeting with the FDA during the first half of 2022.

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As part of our product development activities, we expect to continue to invest in evaluating the potential of OCA in
progressive  non-viral  liver  diseases.  We  are  currently  conducting  a  Phase  3  clinical  trial  in  NASH  patients  with
compensated cirrhosis, known as the REVERSE trial.

We are evaluating the efficacy, safety and tolerability of OCA in combination with bezafibrate in patients with PBC in
a Phase 2 study outside of the United States. In the United States, we have an ongoing Phase 1 study to better characterize
the exposure response of the fixed-dose combination, and we have an open Investigational New Drug (“IND”) application
with the FDA. We are also in the process of initiating a second Phase 2 study in the United States. Our longer-term goal is
developing and seeking regulatory approval for a fixed dose combination regimen in PBC and potentially in other diseases.

In addition, we have other compounds in early stages of research and development in our pipeline, including our INT-
787 compound, an FXR agonist. We are currently evaluating INT-787 in a Phase 1 clinical trial and plan to submit an IND
in the first half of 2022.

Recent Developments

In December 2021, the Company withdrew its MAA with the EMA for conditional approval of OCA for liver fibrosis
due  to  NASH  as  the  established  application  timeline  could  not  be  extended  any  further  to  allow  for  submission  of
additional  safety  and  efficacy  data  being  generated  from  the  REGENERATE  study  and  the  Committee  for  Medicinal
Products for Human Use (the “CHMP”) was not able to determine a positive benefit-risk based on previously submitted
data.  Once  the  additional  data  from  REGENERATE  becomes  available,  the  Company  will  assess  the  possibility  of
submitting a new application to the EMA.

In  February  2022,  we  withdrew  our  application  for  reimbursement  in  France  of  Ocaliva  for  treatment  of  primary
biliary  cholangitis  (“PBC”),  on  account  of  inability  to  reach  mutually  acceptable  pricing  terms  with  the  Economic
Committee  for  Health  Products  (“CEPS”),  the  French  regulator  for  pricing  and  reimbursement  of  pharmaceuticals.  The
French market represents approximately 1% of global net sales for the Company and its consolidated affiliates.

COVID-19

In  March  2020,  we  announced  new  initiatives  intended  to  ensure  business  continuity  and  support  our  employees
during  the  coronavirus  (“COVID-19”)  global  pandemic,  while  continuing  the  critical  activities  necessary  to  bring  our
approved medicines to patients. With respect to our ongoing clinical trials, we are continuing to closely monitor the latest
developments  regarding  the  COVID-19  pandemic  and  together  with  our  contract  research  organizations,  study  sites  and
other partners, have taken measures intended to minimize disruption to these studies. With respect to our supply chain, we
have been working with our third-party manufacturers, distributors and other partners to manage our supply chain activities
and mitigate disruptions to our product supplies. In addition, we continue to closely evaluate the impact of COVID-19 on
our ability to effectively market, sell and distribute Ocaliva for PBC. The long-term effects of COVID-19 are unknown and
we  cannot  presently  predict  the  duration,  scope  or  severity  of  the  potential  effects  of  COVID-19  on  our  operations,
including our clinical trials, regulatory submissions and reviews, supply chain or our ability to generate product sales from
Ocaliva or, if approved, OCA for liver fibrosis due to NASH, and any such effects could have a material adverse impact on
our business, results of operation and financial condition.

Financial Overview

Revenue

We  commenced  our  commercial  launch  of  Ocaliva  for  the  treatment  of  PBC  in  the  United  States  in  June  2016.  In
December  2016,  the  European  Commission  granted  conditional  approval  for  Ocaliva  for  the  treatment  of  PBC  and  we
commenced our European commercial launch in January 2017. Since January 2017, Ocaliva has also received regulatory
approval  in  several  of  our  target  markets  outside  the  United  States  and  Europe,  including  (but  not  limited  to)  Canada,
Israel, and Australia. We sell Ocaliva to a limited number of specialty pharmacies which dispense the product directly to
patients. The specialty pharmacies are referred to as our customers.

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Product Revenue, Net

We recognize revenue upon shipment of Ocaliva to our customers. We provide the right of return to our customers for

unopened product for a limited time before and after its expiration date.

Under Accounting Standards Codification (“ASC”) Topic 606, Revenue from Contracts with Customers (“ASC 606”),
we have written contracts with each of our customers that have a single performance obligation — to deliver products upon
receipt of a customer order — and these obligations are satisfied when delivery occurs and the customer receives Ocaliva.
We  evaluate  the  creditworthiness  of  each  of  our  customers  to  determine  whether  collection  is  reasonably  assured.  We
estimate variable revenue by calculating gross product revenues based on the wholesale acquisition cost that we charge our
customers  for  Ocaliva,  and  then  estimating  our  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and
discounts  related  to  Medicare,  Medicaid  and  other  government  programs,  (ii)  estimated  costs  of  incentives  offered  to
certain indirect customers including patients and (iii) trade allowances, such as invoice discounts for prompt payment and
customer fees.

We  recognized  net  sales  of  Ocaliva  of  $363.5  million,  $312.7  million  and  $249.6  million  for  the  years  ended

December 31, 2021, 2020 and 2019, respectively.

Selling, General and Administrative Expenses

We have incurred and expect to continue to incur significant selling, general and administrative expenses as a result of,
among other initiatives, the commercialization of Ocaliva for PBC in the United States, the United Kingdom, the European
Union and our other target markets. In addition, we have incurred significant selling, general and administrative expenses
and may in the future incur similar expenses in connection with the preparation for the potential commercialization of OCA
for liver fibrosis due to NASH, if approved, and our other future approved products, if any, and any maintenance of our
general and administrative infrastructure in the United States and abroad.

Research and Development Expenses

Since  our  inception,  we  have  focused  significant  resources  on  our  research  and  development  activities,  including
conducting preclinical studies and clinical trials, pursuing regulatory approvals and engaging in other product development
activities. We recognize research and development expenses as they are incurred.

We have incurred and expect to continue to incur significant research and development expenses as a result of, among
other  initiatives,  our  clinical  development  programs  for  OCA  for  PBC  and  NASH,  our  other  earlier  stage  research
programs and our regulatory approval efforts.

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Results of Operations

Comparison of the Years Ended December 31, 2021 and 2020

The following table summarizes our results of operations for the years ended December 31, 2021 and 2020:

Revenue:

Product revenue, net
Total revenue

Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Restructuring

Total operating expenses

Other income (expense):

Interest expense
Gain on extinguishment of debt
Other income, net

Total other income (expense), net

Net loss

Revenues

Year Ended December 31, 

2021

2020

(in thousands)

$  363,468
 363,468

$  312,690
 312,690

 3,100
 230,855
 185,272
 (86)
 419,141

 5,322
 332,493
 191,485
 14,630
 543,930

 (54,419)
 16,511
 2,155
 (35,753)
 (91,426)

 (48,054)
 —
 4,414
 (43,640)
$  (274,880)

$

Product  revenue,  net  was  $363.5  million  and  $312.7  million  for  the  years  ended  December  31,  2021  and  2020,
respectively. For the years ended December 31, 2021 and 2020, product revenue, net was comprised of U.S. Ocaliva net
sales of $260.8 million and $234.0 million, respectively, and ex-U.S. Ocaliva net sales of $102.7 million and $78.7 million,
respectively.  The  increase  in  product  revenues  was  driven  by  operational  growth,  primarily  due  to  higher  unit  sales
volumes and higher net pricing in select markets.

Cost of sales

Cost of sales was $3.1 million and $5.3 million for the years ended December 31, 2021 and 2020, respectively. Our
cost of sales for the years ended December 31, 2021 and 2020 consisted primarily of packaging, labeling, materials and
related expenses.

Selling, general and administrative expenses

Selling, general and administrative expenses were $230.9 million and $332.5 million for the years ended December
31, 2021 and 2020, respectively. The $101.6 million net decrease between periods was primarily driven by decreases in
expenses relating to our activities associated with the potential approval and commercialization of OCA for liver fibrosis
due to NASH.

Research and development expenses

Research and development expenses were $185.3 million and $191.5 million for the years ended December 31, 2021
and  2020,  respectively.  The  $6.2  million  net  decrease  between  periods  was  primarily  driven  by  lower  personnel  costs,
including stock compensation expense and lower costs for NASH related R&D activities, partially offset by the recognition
of lower R&D tax credits and higher costs for cholestasis related R&D activities.

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Restructuring expenses

Restructuring (benefits) expenses were $(0.1) million and $14.6 million for the years ended December 31, 2021 and
2020,  respectively.  The  decrease  between  periods  was  primarily  driven  by  severance  costs  and  other  related  termination
benefits incurred during the year ended December 31, 2020 in conjunction with the 2020 Workforce Plan.

Interest expense

Interest expense was $54.4 million and $48.1 million for the years ended December 31, 2021 and 2020, respectively.
For  the  year  ended  December  31,  2021,  interest  expense  related  to  the  principal  amounts  outstanding  for  the  2023
Convertible Notes, 2026 Convertible Notes and 2026 Convertible Secured Notes. For the year ended December 31, 2020,
interest expense related to the principal amounts outstanding for the 2023 Convertible Notes and 2026 Convertible Notes.

Gain on extinguishment of debt

The  gain  on  extinguishment  of  debt  was  $16.5  million,  related  to  the  exchange  of  the  2023  Convertible  Notes  and

2026 Convertible Notes along with the repurchase of 2023 Convertible Notes.

Other income, net

Other income, net was $2.2 million and $4.4 million for the years ended December 31, 2021 and 2020, respectively.

Such income is primarily attributable to interest income earned on cash, cash equivalents and investment debt securities.

Income taxes

For the years ended December 31, 2021 and 2020, no income tax expense or benefit was recognized. Our deferred tax
assets are comprised primarily of net operating loss carryforwards. We maintain a full valuation allowance on our deferred
tax assets since we have not yet achieved sustained profitable operations. As a result, we have not recorded any income tax
benefit since our inception.

Comparison of the Years Ended December 31, 2020 and 2019

For a comparison of our results of operations for the fiscal years ended December 31, 2020 and December 31, 2019,
see  Part  II,    Item  7.  “Management’s  Discussion  and  Analysis  of  Financial  Condition  and  Results  of  Operations,”  of  our
annual report on Form 10-K for the fiscal year ended December 31, 2020.

Liquidity and Capital Resources

Sources of liquidity

Since inception, we have incurred significant operating losses. We have never been profitable and do not expect to be
profitable  in  the  foreseeable  future.  To  date,  we  have  financed  our  operations  primarily  through  public  and  private
securities offerings, sales of product and payments received under our licensing and collaboration agreements.

Continued  cash  generation  is  highly  dependent  on  the  success  of  our  commercial  product,  Ocaliva,  as  well  as  the

success of our product candidates if approved.

We have devoted substantially all of our resources to the development of our product candidates, including the conduct
of our clinical trials, the launch and commercialization of Ocaliva for PBC, preparation for a potential launch of OCA for
liver fibrosis due to NASH and general and administrative operations, including the protection of our intellectual property.
We intend to continue to develop OCA and our other existing product candidates, alone or in combination, for non-viral
liver diseases. If OCA or any of our other product candidates fails in clinical trials or does not gain or maintain regulatory
approval, or if OCA or any of our other product candidates does not achieve market acceptance, we may never become

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profitable.  Our  net  losses  and  negative  cash  flows  have  had,  and  will  continue  to  have,  an  adverse  effect  on  our
stockholders’ deficit and working capital.

Our  executive  officers  and  our  Board  of  Directors  periodically  review  our  sources  and  potential  uses  of  cash  in
connection  with  our  annual  budgeting  process.  Generally  speaking,  our  principal  funding  source  is  cash  from  operating
activities, and our principal cash requirements include operating expenses and interest payments.

We expect to continue to incur losses for the foreseeable future, and we expect these losses to be significant as we,
among other things, develop and seek regulatory approval for our product candidates, including OCA for liver fibrosis due
to  NASH,  maintain  our  regulatory  approvals  and  commercialize  our  approved  products.  We  believe  our  prospects  and
ability to significantly grow revenues will be dependent on our ability to successfully develop and commercialize OCA for
indications other than PBC, such as NASH, and to identify strategic business development opportunities to leverage our
capabilities  in  rare  diseases.  As  a  result,  we  expect  a  significant  amount  of  resources  to  continue  to  be  devoted  to  our
development programs for OCA and to developing our pipeline.

Cash Flows

The following table sets forth the significant sources and uses of cash for the periods indicated:

2021

Years Ended December 31, 
2020
(in thousands)

2019

Net cash (used in) provided by:

Operating activities
Investing activities
Financing activities
Effect of exchange rate changes
Net increase (decrease) in cash, cash equivalents and restricted cash

$ (41,639) $ (170,026) $  (236,613)
   (188,988)
 162,817
 457,519
 (693)
 (386)
 (1,224)
 31,532
 (9,126) $

 70,726
 1,118
 (1,450)
$  28,755

$

Operating Activities. Net cash used in operating activities of $41.6 million during the year ended December 31, 2021
was primarily a result of our $91.4 million net loss and a net decrease in operating assets and liabilities of $14.4 million,
partially  offset  by  $33.9  million  in  stock-based  compensation,  $13.0  million  for  accretion  of  the  discount  on  the  2023
Convertible Notes, $8.4 million for accretion of the discount on the 2026 Convertible Notes, $9.4 million for accretion on
the 2026 Convertible Secured Notes, $5.8 million for non-cash operating lease costs and $3.0 million of depreciation. Cash
flows for the year ended December 31, 2021 include net cash receipts of $4.0 million reflecting payments from the HMRC
for the U.K. R&D tax credit claims.

Net cash used in operating activities of $170.0 million during the year ended December 31, 2020 was primarily a result
of our $274.9 million net loss, partially offset by $60.8 million in stock-based compensation, $16.6 million for accretion of
the discount on the 2023 Convertible Notes, $9.4 million for accretion of the discount on the 2026 Convertible Notes, $6.1
million for non-cash operating lease costs, $3.1 million of depreciation and a net increase in operating assets and liabilities
of  $2.0  million.  Cash  flows  for  the  year  ended  December  31,  2020  include  cash  receipts  of  $20.7  million  reflecting
payments from the HMRC for the U.K. R&D tax credit claims.

Net cash used in operating activities of $236.6 million during the year ended December 31, 2019 was primarily a result
of our $344.7 million net loss and a gain on lease termination of $2.0 million, partially offset by $56.0 million in stock-
based compensation, a net increase in operating assets and liabilities of $19.3 million, $15.3 million for accretion of the
discount  on  the  2023  Convertible  Notes,  $5.9  million  for  accretion  of  the  discount  on  the  2026  Convertible  Notes,  $5.4
million for non-cash operating lease costs, $3.7 million of depreciation and $2.7 million for loss on the disposal of fixed
assets.

Investing Activities. For the year ended December 31, 2021, net cash provided by investing activities primarily reflects
the sales and maturities of investment debt securities of $420.6 million, partially offset by the purchases of investment debt
securities of $349.5 million.

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For  the  year  ended  December  31,  2020,  net  cash  provided  by  investing  activities  primarily  reflects  the  sales  and
maturities of investment debt securities of $497.4 million, partially offset by the purchases of investment debt securities of
$330.7 million.

For  the  year  ended  December  31,  2019,  net  cash  used  in  investing  activities  primarily  reflects  the  purchases  of

investment debt securities of $603.0 million, partially offset by the sales of investment debt securities of $415.2 million.

Financing  Activities.  Net  cash  provided  by  financing  activities  in  the  year  ended  December  31,  2021  consisted
primarily of $116.7 million of proceeds, net of issuance costs, from the sale of 2026 Convertible Secured Notes, offset by
payments of $75.8 million for the repurchase of common stock and $38.1 million for the repurchase of 2023 Convertible
Notes.

Net cash used in financing activities in the year ended December 31, 2020 consisted primarily of $2.0 million from
payments  of  employee  withholding  taxes  related  to  stock-based  awards  offset  by  $1.3  million  of  net  proceeds  from  the
exercise of options to purchase common stock.

Net  cash  provided  by  financing  activities  in  the  year  ended  December  31,  2019  consisted  primarily  of  net  proceeds
received from the 2019 Public Offering and 2019 Concurrent Private Placement in May 2019 of $227.3 million and net
proceeds from the issuance of the 2026 Convertible Notes of $223.4 million.

2021 Debt Refinancing, Retirement, and New Money Investment

In August 2021, we agreed with certain institutional holders of our 2023 Convertible Notes and our 2026 Convertible
Notes maturing May 15, 2026, to exchange existing notes of both series at a discount for new 2026 Convertible Secured
Notes maturing February 15, 2026, and secured by a first priority security interest in substantially all assets of Intercept
Pharmaceuticals,  Inc.  and  of  any  subsidiaries  that  meet  certain  threshold  requirements  to  become  guarantors.  The
noteholders  (1)  exchanged  $306.5  million  of  2023  Convertible  Notes  for  $292.4  million  of  new  notes,  (2)  exchanged
$114.7 million of 2026 Convertible Notes for $90.0 million of new notes, and also (3) subscribed to buy $117.6 million of
new notes for cash. We thereby issued $500.0 million of 2026 Convertible Secured Notes at an interest rate of 3.50%. We
received  cash  proceeds  of  $117.6  million.  We  also  paid  our  financial  advisory  fee  by  issuing  769,823  new  shares  of
common  stock.  Further,  in  connection  with  the  exchange  and  sale,  we  bought  back  approximately  4.5  million  shares  of
common stock for $75.8 million in cash.

In  September  2021,  we  agreed  with  certain  institutional  holders  to  buy  back  $39.9  million  of  our  2023  Convertible

Notes at a discount.

On  account  of  these  transactions,  we  reduced  our  2023  Convertible  Notes  outstanding  by  approximately  75%  from
$460.0 million to $113.7 million and our 2026 Convertible Notes outstanding by approximately 50% from $230.0 million
to $115.3 million.

Future Funding Requirements

We are currently developing OCA for additional indications, including NASH, and other product candidates through
various  stages  of  clinical  and  preclinical  development.  Developing  pharmaceutical  products,  including  conducting
preclinical  studies  and  clinical  trials,  is  expensive.  In  addition,  we  have  incurred  and  anticipate  that  we  will  continue  to
incur significant research and development, product sales, marketing, manufacturing and distribution expenses relating to
the commercialization of Ocaliva for PBC. As part of our longer-term strategy, we anticipate that we will incur significant
expenses  in  connection  with  our  research  and  development  efforts,  the  commercialization  of  our  other  products  such  as
OCA for liver fibrosis due to NASH, if approved, and the maintenance of our general and administrative infrastructure in
the  United  States  and  abroad.  We  may  also  engage  in  business  development  activities  that  involve  potential  in-  or  out-
licensing of products or technologies or acquisitions of other products, technologies or businesses.

As  of  December  31,  2021,  we  had  $429.4  million  in  cash,  cash  equivalents,  restricted  cash  and  investment  debt

securities. We currently expect to continue to incur significant operating expenses in the fiscal year ending December 31,

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2022. These expenses are planned to support, among other initiatives, the continued commercialization of Ocaliva for PBC
in the United States and our other markets, our continued clinical development of OCA for PBC and NASH and our other
earlier stage research and development programs. Although we believe that our existing capital resources, together with our
net sales of Ocaliva for PBC, will be sufficient to fund our anticipated operating requirements for the next twelve months
following the filing of this report, we may need to raise additional capital to fund our operating requirements beyond that
period. In recent quarters we have significantly reduced our cash burn and remain in a stable cash position. Cash in excess
of  immediate  requirements  is  invested  in  accordance  with  our  investment  policy,  primarily  with  a  view  to  liquidity  and
capital  preservation.  As  of  December  31,  2021,  our  funds  are  primarily  held  in  U.S.  treasuries,  corporate  and  municipal
bonds, commercial paper, and money market accounts.

We successfully exchanged the majority of our near-term debt to address the maturity of 2023 convertible notes. While
we  have  retired  approximately  75%  of  our  2023  Convertible  Notes,  we  still  have  $113.7  million  of  them  scheduled  to
mature on July 1, 2023, and $615.3 million of convertible notes scheduled to mature in 2026, all of which will need to be
paid off or refinanced, if not converted. Furthermore, in light of our receipt of the CRL from the FDA in June 2020 with
respect  to  our  NDA  for  OCA  for  liver  fibrosis  due  to  NASH  and  the  numerous  risks  and  uncertainties  associated  with
pharmaceutical  product  development  and  commercialization,  any  delays  in,  or  unanticipated  costs  associated  with,  our
development, regulatory or commercialization efforts could significantly increase the amount of capital required by us to
fund  our  operating  requirements.  Accordingly,  we  may  seek  to  access  the  public  or  private  capital  markets  whenever
conditions are favorable, to issue new securities, or to refinance or repurchase existing securities, even if we do not have an
immediate need for additional capital at that time.

Our forecasts regarding the period of time that our existing capital resources will be sufficient to meet our operating
requirements  and  the  timing  of  our  future  funding  requirements,  both  near  and  long-term,  will  depend  on  a  variety  of
factors, many of which are outside of our control. Such factors include, but are not limited to, those factors listed above
under “Cautionary Note Regarding Forward-Looking Statements”.

We have no committed external sources of funding and additional funds may not be available when we need them on
terms that are acceptable to us, or at all. If adequate funds are not available to us, we may not be able to make scheduled
debt payments on a timely basis, or at all, and may be required to delay, limit, reduce or cease our operations.

Future Contractual Obligations

Our  estimated  future  obligations  as  of  December  31,  2021  include  both  current  and  long  term  obligations.  For  our
long-term debt as noted in Note 9—Long-Term Debt, we have short-term obligations for interest payments of $23.5 million
and  long-term  obligations  of  $793.3  million  for  interest  and  principal  payments.  Under  our  operating  leases  as  noted  in
Note 7—Leases, we have short-term obligations of $3.4 million and long-term obligations of $4.8 million.

We enter into contracts in the normal course of business with contract research organizations for our clinical trials. We
may incur expenses related to clinical studies of our product candidates. The timing and amounts of these disbursements
are  contingent  upon  the  achievement  of  certain  milestones,  patient  enrollment  and  services  rendered  or  as  expenses  are
incurred  by  the  CROs  or  clinical  trial  sites.  Therefore,  we  cannot  estimate  the  potential  timing  and  amount  of  these
payments.

We source the manufacture and commercial supply of API from manufacturers, for use in Ocaliva and, if approved,
OCA for liver fibrosis due to NASH. Our contracts either do not require us to purchase a specific percentage of our annual
commercial  requirements  of  API,  are  made  on  a  purchase  order  basis  or  may  require  future  purchase  obligations  in  the
event  of  the  achievement  of  agreed  regulatory  and  product  development  milestones.  We  cannot,  at  this  time,  determine
when  or  if  the  related  milestones  will  be  achieved  or  whether  the  events  triggering  the  commencement  of  payment
obligations will occur.

Critical Accounting Policies and Estimates

Our management’s discussion and analysis of our financial condition and results of operations is based on our audited

consolidated financial statements, which we have prepared in accordance with accounting principles generally accepted in

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the  United  States  of  America.  The  preparation  of  our  audited  consolidated  financial  statements  requires  us  to  make
estimates  and  judgments  that  affect  the  reported  amounts  of  our  assets,  liabilities,  revenues  and  expenses.  We  have
identified  certain  estimates  as  critical  to  our  business  operations  and  the  understanding  of  our  past  or  present  results  of
operations  related  to  (i)  revenue  recognition  (ii)  stock-based  compensation  (iii)  issuance  of  convertible  debt  and  (iv)
income taxes. These estimates are considered critical because they had a material impact, or they have the potential to have
a  material  impact,  on  our  consolidated  financial  statements  and  because  they  require  us  to  make  significant  judgments,
assumptions or estimates. We base our estimates on historical experience and on various other factors that we believe are
reasonable  under  the  circumstances  based  on  information  available  at  the  time  they  were  made.  We  evaluate  these
estimates  and  judgments  on  an  ongoing  basis.  However,  our  actual  results  could  differ  from  these  estimates,  and  these
differences may be material.

Revenue Recognition

Product Revenue, Net

Under ASC 606, we have written contracts with each of our customers that have a single performance obligation — to
deliver  products  upon  receipt  of  a  customer  order  —  and  these  obligations  are  satisfied  when  delivery  occurs  and  the
customer receives Ocaliva. We evaluate the creditworthiness of each of our customers to determine whether collection is
reasonably assured. The wholesale acquisition cost that we charge our customers for Ocaliva is adjusted to arrive at our
estimated  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and  discounts,  (ii)  estimated  costs  of
incentives offered to certain indirect customers including patients, and (iii) trade allowances, such as invoice discounts for
prompt payment and customer fees.

Rebates and Discounts

We  contract  with  the  Centers  for  Medicare  &  Medicaid  Services  and  other  government  agencies  to  make  Ocaliva
available to eligible patients. As a result, we estimate any rebates and discounts and deduct these estimated amounts from
our gross product revenues at the time the revenues are recognized. Our estimates of rebates and discounts are based on the
government mandated discounts, which are statutorily-defined and applicable to these government funded programs, and
our historical experience with actual payments and redemptions. These estimates are recorded in accounts payable, accrued
expenses  and  other  liabilities  on  our  consolidated  balance  sheets.  To  date,  actual  government  rebates  have  not  differed
materially from our estimates.

We have been distributing and selling Ocaliva in Europe through our EU marketing authorization since 2017 and are
engaged in ongoing price discussions regarding the final price of Ocaliva within one of those jurisdictions. We recognize
net  product  revenues  based  on  our  estimate  of  consideration  we  expect  to  retain  through  final  negotiations  in  that
jurisdiction that will not be subject to a significant reversal. Our estimate is based on benchmarks of pricing approved in
other  relevant  European  jurisdictions  and  relevant  information  in  the  ongoing  negotiations.  We  expect  the  difference
between the amounts collected at the invoiced price and the final price for OCA will be returned to the local government. If
our estimates regarding the amounts to be refunded to the government change, we will reflect the effect of the change in
estimate  in  net  product  revenues  in  the  period  in  which  the  change  in  estimate  occurs  and  will  include  any  adjustments
against  all  prior  sales.  These  estimates  are  recorded  in  accounts  payable,  accrued  expenses  and  other  liabilities  on  our
consolidated balance sheets.

Other Incentives

Other incentives that we offer to indirect customers include co-pay assistance cards provided by us for PBC patients
who  reside  in  states  that  permit  co-pay  assistance  programs.  Our  co-pay  assistance  program  is  intended  to  reduce  each
participating patient’s portion of the financial responsibility for Ocaliva purchase price to a specified dollar amount. We
estimate the amount of co-pay assistance provided to eligible patients based on the terms of the program when product is
dispensed  by  the  specialty  pharmacies  to  the  patients.  These  estimates  are  based  on  historical  redemption  and  payment
information  provided  by  third-party  claims  processing  organizations  along  with  estimated  future  redemptions  and  are
recorded in accounts payable, accrued expenses and other liabilities on our consolidated balance sheets.

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Trade Allowances

We  provide  invoice  discounts  on  Ocaliva  sales  to  certain  of  our  customers  for  prompt  payment  and  record  these
discounts as a reduction to gross product revenues. These discounts are based on contractual terms. We anticipate that our
customers will earn these discounts and fees and, therefore, we deduct the full amount of these discounts and fees from
total gross product revenues. Reserves for prompt payment discounts are recorded in the same period the related revenue is
recognized, resulting in a reduction of product revenue and accounts receivable.

Returns

The Company provides the right of return to its customers for unopened product for a limited time before and after its
expiration date. Returns are estimated based on historical experience and product shelf lives. In arriving at our estimate, the
assessment considered the product type, life-cycle, price, distribution channel, channel inventory and the customer returns
policy  along  with  benchmarking  against  industry  data  specific  to  the  pharmaceutical  distribution  industry.  Historically,
actual returns have not differed materially from our estimates.

The  potential  of  our  estimates  to  vary  due  to  sensitivity  differs  by  program,  type  of  customer  and/or  geographic
location. Estimates associated with government programs have a higher risk of being subject to adjustment because of the
time delay between recording the accrual and the final settlement. These reserves reflect our best estimates of the amount
of consideration to which the relevant third party is entitled to based on the terms of the applicable contract. The amount of
variable consideration included in the transaction price may be constrained and is included in the net sales price only to the
extent that it is probable that a significant reversal in the amount of the cumulative revenue recognized will not occur in a
future  period.  Historically,  adjustments  to  these  estimates  to  reflect  actual  results  or  updated  expectations  have  not  been
material. Actual amounts of consideration ultimately received may differ from our estimates. If actual results in the future
vary  from  our  estimates,  we  adjust  these  estimates,  which  would  affect  net  product  revenues  and  earnings  in  the  period
such variances become known.

Valuation of Stock-Based Compensation

We account for stock-based compensation in accordance with ASC Topic 718, Compensation — Stock Compensation.
We estimate the fair value of stock option awards using the Black-Scholes option pricing model on the date of the grant.
Valuation  models,  like  the  Black-Scholes-Merton  model,  require  the  use  of  subjective  assumptions  that  could  materially
impact the estimation of fair value and related compensation expense to be recognized. The Black-Scholes option pricing
model requires the use of assumptions, including with respect to price volatility of the underlying stock, assumed dividend
yield, expected term of the options and the risk-free interest rate, as described below:

• The expected volatility is estimated based on actual daily historical volatility information of our own ordinary shares
equal to the expected term of our options.

• The assumed dividend yield is based on not issuing any dividends and not expecting to issue any dividends over the
life of the options. As a result, we have estimated the dividend yield to be zero.

• The expected term of options granted represents the period of time the options are expected to be outstanding and is
based on the simplified method, whereby the expected term equals the arithmetic average of the vesting term and the
original contractual term of the option (generally 10 years).

• The risk-free interest rate is based on the yield curve for U.S. Treasury securities at the date of grant with maturity
dates approximately equal to the expected term of the award at the grant date.

There  have  been  no  material  changes  in  our  estimates  or  assumptions  since  the  prior  reporting  period.  We  do  not

believe there is a reasonable likelihood there will be a material change in the future estimates or assumptions.

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We  expect  to  continue  to  grant  stock  options  and  other  stock-based  awards  and  the  impact  of  stock-based
compensation may fluctuate in future periods due to changes in the value of our common stock, changes to our headcount
and the number and value of awards granted.

Convertible Senior Notes

The Convertible Notes are accounted for in accordance with ASC Subtopic 470-20, Debt with Conversion and Other
Options. ASC Subtopic 470-20 requires the issuer of convertible debt that may be settled in shares or cash upon conversion
at  the  issuer’s  option,  such  as  the  Convertible  Notes,  to  account  for  the  liability  (debt)  and  equity  (conversion  option)
components separately. The value assigned to the debt component is the estimated fair value, as of the issuance date, of a
similar debt instrument without the conversion option. The amount of the equity component (and resulting debt discount) is
calculated  by  deducting  the  fair  value  of  the  liability  component  from  the  principal  amount  of  the  convertible  debt
instrument. The resulting debt discount is amortized as additional non-cash interest expense over the expected life of the
notes utilizing the effective interest method.

 The carrying amount of the liability component was calculated by measuring the fair value of a similar liability that
does not have an associated convertible feature using the income approach. The allocation was performed in a manner that
reflected our non-convertible borrowing rate for similar debt. For the income-based approach, we use a convertible bond
lattice model that includes assumptions such as volatility and the risk-free rate. The equity component is not remeasured as
long as it continues to meet the conditions for equity classification.

The  estimate  is  not  expected  to  have  any  impact  on  the  future  results  given  the  adoption  of  the  new  ASU  2020-06
standard will reclass the amounts of the equity components into the liability components. For additional information, see
Note 9 to our audited consolidated financial statements included elsewhere in this Annual Report on Form 10-K.

Income Taxes

We utilize the asset and liability method of accounting for income taxes. Under this method, deferred tax assets and
liabilities are determined based on the difference between the financial statement carrying amounts and tax bases of assets
and liabilities using enacted tax rates in effect for years in which the temporary differences are expected to reverse.

We determine the need for a valuation allowance by assessing the probability of realizing deferred tax assets, taking
into consideration all available positive and negative evidence, including historical operating results, expectations of future
taxable  income,  carryforward  periods  available,  various  income  tax  strategies  and  other  relevant  factors.  Judgment  is
required in making this assessment and to the extent future expectations change, we would have to assess the recoverability
of  our  deferred  assets  at  that  time.  At  December  31,  2021  and  2020,  we  maintained  a  full  valuation  allowance  on  our
deferred tax assets.

Our tax returns are subject to examination by U.S. Federal, state, and foreign taxing jurisdictions. The impact of an
uncertain tax position taken or expected to be taken on an income tax return must be recognized in our financial statements
at the largest amount that is more likely than not to be sustained. An uncertain income tax position will not be recognized
in  our  financial  statements  unless  it  is  more  likely  than  not  to  be  sustained.  We  consider  the  facts,  circumstances,  and
information available at the reporting date. The level of evidence that is necessary and appropriate to support an entity’s
assessment of the technical merits of a tax position is a matter of judgment that depends on all available information. As a
result, whether a tax position will ultimately be sustained may be uncertain. At December 31, 2021 and 2020, we had no
reserves for unrecognized tax benefits.

Recent Accounting Pronouncements

See Note 2 to our audited consolidated financial statements included elsewhere in this Annual Report on Form 10-K
for  a  full  description  of  recent  accounting  pronouncements  including  the  respective  expected  dates  of  adoption  and
expected effects, if any, on our results of operations and financial condition.

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Item 7A.  Quantitative and Qualitative Disclosures about Market Risk

Our primary exposure to market risk is interest rate sensitivity, which is affected by changes in the general level of
U.S.  interest  rates.  We  currently  do  not  hedge  interest  rate  exposure  because  of  the  short-term  maturities  of  our  cash
equivalents and investment debt securities. Our investment debt securities are subject to interest rate risk and will fall in
value if market interest rates increase. At any time, sharp changes in interest rates can affect the fair value of the investment
portfolio and its interest earnings. We do not believe that an increase in market rates would have any significant impact on
the realized value of our investment debt securities. If a hypothetical increase in interest rates of 100 basis points were to
have occurred on December 31, 2021, this change would not have had a material effect on the fair value of our investment
portfolio as of that date due to the conservative and short-term nature of these investments.

We  do  not  believe  that  our  cash,  cash  equivalents  and  investment  debt  securities  have  significant  risk  of  default  or
illiquidity. We maintain an investment portfolio in accordance with our investment policy. The primary objectives of our
investment  policy  are  to  preserve  principal  and  maintain  proper  liquidity  to  meet  operating  needs.  Although  our
investments are subject to credit risk, our investment policy specifies credit quality standards for our investments, maturity
restrictions  and  limits  the  amount  of  credit  exposure  from  any  single  issue  or  issuer.  While  we  believe  our  cash,  cash
equivalents and investment debt securities do not contain excessive risk, we cannot provide absolute assurance that, in the
future,  our  investments  will  not  be  subject  to  adverse  changes  in  market  value.  In  addition,  we  maintain  significant
amounts of cash and cash equivalents at one or more financial institutions that are in excess of federally insured limits.

As  a  result  of  our  ex-U.S.  operations,  we  contract  with  CROs,  investigational  sites,  suppliers,  facilities,  marketing
firms  and  other  vendors  and  suppliers  in  Europe  and  internationally.  We  are  therefore  subject  to  fluctuations  in  foreign
currency exchange rates in connection with these agreements. We do not hedge our foreign currency exchange rate risk.

Inflation generally affects us by increasing our cost of labor and clinical trial costs. We do not believe that inflation has

had a material effect on our results of operations during 2021, 2020 or 2019.

Item 8.   Financial Statements and Supplementary Data

The financial statements required to be filed pursuant to this Item 8 are appended to this Annual Report on Form 10-K
and  incorporated  by  reference  herein.  An  index  of  those  financial  statements  is  set  forth  under  Item  15.  “Exhibits  and
Financial Statement Schedules”.

Item 9.   Changes in and Disagreements With Accountants on Accounting and Financial Disclosure

None.

Item 9A.  Controls and Procedures

Evaluation of Disclosure Controls and Procedures

Our  Chief  Executive  Officer  and  Chief  Financial  Officer  evaluated  the  effectiveness  of  our  disclosure  controls  and
procedures  as  of  December  31,  2021.  The  term  “disclosure  controls  and  procedures,”  as  defined  in  Rules  13a-15(e)  and
15d-15(e)  under  the  Exchange  Act,  means  controls  and  other  procedures  of  a  company  that  are  designed  to  ensure  that
information  required  to  be  disclosed  by  a  company  in  the  reports  that  it  files  or  submits  under  the  Exchange  Act  is
recorded, processed, summarized and reported, within the time periods specified in the SEC’s rules and forms. Disclosure
controls and procedures include, without limitation, controls and procedures designed to ensure that information required
to  be  disclosed  by  a  company  in  the  reports  that  it  files  or  submits  under  the  Exchange  Act  is  accumulated  and
communicated  to  the  company’s  management,  including  its  principal  executive  and  principal  financial  officers,  as
appropriate  to  allow  timely  decisions  regarding  required  disclosure.  Management  recognizes  that  any  controls  and
procedures, no matter how well designed and operated, can provide only reasonable assurance of achieving their objectives
and  management  necessarily  applies  its  judgment  in  evaluating  the  cost-benefit  relationship  of  possible  controls  and
procedures.  Based  on  the  evaluation  of  our  disclosure  controls  and  procedures  as  of  December  31,  2021,  our  Chief
Executive Officer and Chief

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Financial Officer concluded that, as of such date, our disclosure controls and procedures were effective at the reasonable
assurance level.

Management’s Report on Internal Control Over Financial Reporting

Our  management  is  responsible  for  establishing  and  maintaining  adequate  internal  control  over  financial  reporting.
Internal control over financial reporting is defined in Rules 13a-15(f) and 15d-15(f) under the Exchange Act, as a process
designed by, or under the supervision of, the company’s principal executive and principal financial officers and effected by
the  company’s  board  of  directors,  management  and  other  personnel,  to  provide  reasonable  assurance  regarding  the
reliability  of  financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles and includes those policies and procedures that: (i) pertain to the maintenance of
records that in reasonable detail accurately and fairly reflect the transactions and dispositions of the assets of the company;
(ii) provide reasonable assurance that transactions are recorded as necessary to permit preparation of financial statements in
accordance  with  generally  accepted  accounting  principles,  and  that  receipts  and  expenditures  of  our  company  are  being
made  only  in  accordance  with  authorizations  of  management  and  directors  of  the  company;  and  (iii)  provide  reasonable
assurance regarding prevention or timely detection of unauthorized acquisition, use, or disposition of our company’s assets
that could have a material effect on the financial statements.

All  internal  controls,  no  matter  how  well  designed,  have  inherent  limitations.  Therefore,  even  those  systems
determined  to  be  effective  can  provide  only  reasonable  assurance  with  respect  to  consolidated  financial  statement
preparation and presentation. Because of its inherent limitations, internal control over financial reporting may not prevent
or detect misstatements. Also, projections of any evaluation of effectiveness to future periods are subject to the risk that
controls may become inadequate because of changes in conditions, or that the degree of compliance with the policies or
procedures may deteriorate.

Our  management,  with  the  participation  of  our  Chief  Executive  Officer  and  Chief  Financial  Officer,  assessed  the
effectiveness of our internal control over financial reporting as of December 31, 2021, based on criteria established in the
Internal Control — Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of the Treadway
Commission (COSO). Based on that assessment, management concluded that our internal control over financial reporting
was effective as of December 31, 2021.

Attestation Report of Independent Registered Public Accounting Firm

The effectiveness of our internal control over financial reporting as of December 31, 2021 has been audited by KPMG
LLP, an independent registered public accounting firm, as stated in their report included elsewhere in this Annual Report
on Form 10-K.

Changes in Internal Control Over Financial Reporting

There  were  no  changes  in  our  internal  control  over  financial  reporting  that  occurred  during  the  quarter  ended
December  31,  2021  that  have  materially  affected,  or  are  reasonably  likely  to  materially  affect,  our  internal  control  over
financial reporting.

Item 9B.  Other Information

Not applicable.

Item 9C.  Disclosure Regarding Foreign Jurisdictions that Prevent Inspections

None.

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Item 10.  Directors, Executive Officers and Corporate Governance

PART III

We have adopted a Global Code of Business Conduct as our “code of ethics,” as defined by regulations promulgated
under the Securities Act of 1933, as amended, and the Securities Exchange Act of 1934, as amended, which applies to our
directors, officers and employees, including our principal executive officer, principal financial officer, principal accounting
officer  or  controller,  or  persons  performing  similar  functions.  The  Global  Code  of  Business  Conduct  is  available  on  our
website  at  www.interceptpharma.com  in  the  Investors  &  Media  section  under  “Corporate  Governance.”  We  intend  to
satisfy  the  disclosure  requirement  under  Item  5.05  of  Form  8-K  regarding  any  future  amendment  to,  or  waiver  from,  a
provision of the Global Code of Business Conduct that applies to our principal executive officer, principal financial officer,
principal  accounting  officer  or  controller,  or  persons  performing  similar  functions  by  posting  such  information  on  our
website at www.interceptpharma.com in the Investors & Media section under “Corporate Governance.” The references to
www.interceptpharma.com herein are inactive textual references only, and the information found on our internet website is
not incorporated by reference into this Annual Report on Form 10-K or any other report we file with or furnish to the SEC.

The remainder of the information required by this item is incorporated by reference to our definitive proxy statement
related to our 2022 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after
the end of the fiscal year covered by this Annual Report on Form 10-K.

Item 11.  Executive Compensation

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2022 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

Item 12.  Security Ownership of Certain Beneficial Owners and Management and Related Stockholder Matters

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2022 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

Item 13.  Certain Relationships and Related Transactions, and Director Independence

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2022 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

Item 14.  Principal Accounting Fees and Services

The  information  required  by  this  item  is  incorporated  by  reference  to  our  definitive  proxy  statement  related  to  our
2022 Annual Meeting of Stockholders, to be filed pursuant to Regulation 14A not later than 120 days after the end of the
fiscal year covered by this Annual Report on Form 10-K.

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PART IV

Item 15.  Exhibits and Financial Statement Schedules

(a) 1. Index to Consolidated Financial Statements

Reports of Independent Registered Public Accounting Firm
Consolidated Balance Sheets
Consolidated Statements of Operations
Consolidated Statements of Comprehensive Loss
Consolidated Statements of Changes in Stockholders’ (Deficit) Equity
Consolidated Statements of Cash Flows
Notes to Consolidated Financial Statements

2. Index to Consolidated Financial Statements

F-2
F-5
F-6
F-7
F-8
F-9
F-11

Financial  statement  schedules  have  been  omitted  from  this  Annual  Report  on  Form  10-K  because  they  are  not
applicable,  not  required  or  the  information  required  is  set  forth  in  the  audited  consolidated  financial  statements  or
accompanying notes.

3. Exhibits

The exhibits filed or furnished as part of this Annual Report on Form 10-K are set forth in the Exhibit Index below,

which is incorporated herein by reference.

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Exhibit Index

Incorporated herein by reference

Exhibit
Number     

3.1

3.2

4.1

4.2

4.3

4.4

4.5

4.6

4.7

4.8

4.9

Restated Certificate of Incorporation, as amended

Exhibit Description

Form†
Form 10-Q

     Exhibit     
3.1

Filing Date
August 10, 2020

Restated Bylaws

Form of Common Stock Certificate

Indenture, dated as of July 6, 2016, between the Registrant
and U.S. Bank National Association, as trustee

First Supplemental Indenture (including the Form of
Note), dated as of July 6, 2016, between the Registrant and
U.S. Bank National Association, as trustee

Form of Senior Indenture

Form of Subordinated Indenture

Form of Senior Note

Form of Subordinated Note

Form 10-Q

Form S-8(1)

Form 8-K

Form 8-K

Form S-3(2)

Form S-3(2)

Form S-3(2)

Form S-3(2)

3.2

4.3

4.1

4.2

4.1

4.2

4.3

4.4

August 10, 2020

November 7, 2012

July 6, 2016

July 6, 2016

May 10, 2017

May 10, 2017

May 10, 2017

May 10, 2017

Securities Purchase Agreement, dated April 4, 2018,
between the Registrant and the purchasers named therein

Form 8-K

10.1

April 10, 2018

Securities Purchase Agreement, dated May 8, 2019,
between the Registrant and the purchasers named therein

Form 8-K

10.1

May 14, 2019

4.10

Second Supplemental Indenture (including the Form of
Note), dated as of May 14, 2019, between the Registrant
and U.S. Bank National Association, as trustee

4.11*

Description of Securities of the Registrant

Form 8-K

4.2

May 14, 2019

4.12

4.13

4.14

Indenture, dated as of August 17, 2021, between the
Registrant and U.S. Bank National Association, as trustee

Form 8-K

4.1

August 23, 2021

First Supplemental Indenture (including the Form of
Note), dated as of August 17, 2021, between the
Registrant and U.S. Bank National Association, as trustee
and as collateral agent

Security Agreement, dated as of August 17, 2021, among
the Registrant, the Guarantors that may from time to time
be a party thereto and U.S. Bank National Association, as
collateral agent

Form 8-K

4.2

August 23, 2021

Form 8-K

10.1

August 23, 2021

10.1#

Intercept Pharmaceuticals, Inc. 2012 Equity Incentive Plan

Form S-1/A(3)

10.2.1

September 27, 2012

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10.2#

Form of Stock Option Grant Notice and Agreement for
Directors

Form 10-Q

10.1

August 10, 2020

10.3#

Form of Stock Option Grant Notice and Agreement for
Employees and Consultants

Form 10-K

10.3

February 25, 2020

10.4#

Form of Restricted Stock Unit Award Grant Notice and
Agreement for Directors

Form 10-Q

10.2

August 10, 2020

10.5#

Form of Restricted Stock Unit Award Grant Notice and
Agreement for Employees and Consultants

Form 10-K

10.5

February 25, 2020

10.6#

Form of Restricted Stock Award Grant Notice and
Agreement for Directors

10.7#

Form of Restricted Stock Award Grant Notice and
Agreement for Employees and Consultants

10.8#

Form of Performance Stock Unit Grant Notice and
Agreement

Form 10-Q

10.3 

May 9, 2014

Form 10-Q

10.4 

May 9, 2014

Form 10-K

10.8 

February 25, 2020

10.9#

Form of Performance Share Grant Notice and Agreement

Form 10-Q

10.6 

May 10, 2018

10.10#

2022 Cash Incentive Plan

Form 8-K

10.1

January 31, 2022

10.11#

2022 Cash Incentive Plan - Form of Performance-Based
Award Agreement

Form 8-K

10.2

January 31, 2022

10.12# Employment Agreement, effective April 14, 2017, between

Form 10-Q

10.1 

August 3, 2017

the Registrant and David Ford

10.13# Employment Agreement, effective February 6, 2018,
between the Registrant and Gail Cawkwell

Form 10-Q

10.2 

August 8, 2019

10.14# Amended and Restated Employment Agreement, dated as
of December 9, 2020, between the Registrant and Jerome
Durso

Form 8-K

10.1

December 10, 2020

10.15# Employment Agreement, effective as of December 18,

Form 10-K

10.21

February 25, 2021

2020, between the Registrant and Jared Freedberg

10.16# Employment Agreement, effective January 4, 2021,

Form 10-Q

10.1

May 6, 2021

between the Registrant and Bryan Ball

10.17# Employment Agreement, effective February 15, 2021,
between the Registrant and Linda Richardson

Form 10-Q

10.3

May 6, 2021

10.18# Employment Agreement, effective May 17, 2021, between

Form 10-Q

10.1

July 29, 2021

the Registrant and Andrew Saik

10.19# Employment Agreement, effective June 2, 2021, between

Form 10-Q

10.2

July 29, 2021

the Registrant and M. Michelle Berrey

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Table of Contents

10.20

Base Call Option Confirmation, dated June 30, 2016,
between the Registrant and Royal Bank of Canada

Form 8-K

10.1 

July 6, 2016

10.21

Base Call Option Confirmation, dated June 30, 2016,
between the Registrant and UBS AG, London Branch

Form 8-K

10.3 

July 6, 2016

10.22

Base Call Option Confirmation, dated June 30, 2016,
between the Registrant and Credit Suisse Capital LLC

Form 8-K

10.5 

July 6, 2016

10.23 Additional Call Option Confirmation, dated July 1, 2016,
between the Registrant and Royal Bank of Canada

Form 8-K

10.2 

July 6, 2016

10.24 Additional Call Option Confirmation, dated July 1, 2016,

Form 8-K

10.4 

July 6, 2016

between the Registrant and UBS AG, London Branch

10.25 Additional Call Option Confirmation, dated July 1, 2016,

Form 8-K

10.6 

July 6, 2016

between the Registrant and Credit Suisse Capital LLC

10.26

Lease Agreement between The Irvine Company LLC and
the Registrant, dated May 1, 2014

Form 8-K

10.1 

May 7, 2014

10.27

Second Amendment to Lease, dated as of July 19, 2016,
between the Registrant and Irvine Eastgate Office II LLC

Form 10-Q

10.7 

November 9, 2016

10.28

Third Amendment to Lease, dated as of June 21, 2018,
between the Registrant and Irvine Eastgate Office II LLC

Form 10-Q

10.1 

August 7, 2018

10.29

Fourth Amendment to Lease, dated as of October 30, 2018,
between the Registrant and Irvine Eastgate Office II LLC

Form 10-Q

10.1 

November 1, 2018

10.30 Underlease between the Registrant, Intercept Pharma
Europe Ltd. and Performing Right Society, Ltd., dated
January 22, 2016

Form 10-K

10.12 

February 29, 2016

10.31

Lease Agreement, dated December 7, 2016, between the
Registrant and Legacy Yards Tenant LP

Form 10-K

10.17 

March 1, 2017

10.32

First Amendment to Lease Agreement, dated June 27,
2017, between the Registrant and Legacy Yards Tenant LP

Form 10-Q

10.1 

November 6, 2017

10.33

Second Amendment to Lease, dated June 22, 2018,
between the Registrant and Legacy Yards Tenant LP

Form 10-Q

10.2 

August 7, 2018

10.34

Third Amendment to Lease, dated November 1, 2019,
between the Registrant and Legacy Yards Tenant LP

Form 10-Q

10.1

November 5, 2019

10.35++ Commercial Manufacturing and Supply Agreement, dated
August 12, 2016, between the Registrant and PharmaZell
GMBH

Form 10-K

10.39

February 25, 2021

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Table of Contents

10.36+ Amendment #1 to Manufacturing and Supply Agreement,

Form 10-K

10.2.1

February 28, 2018

dated December 12, 2017, between the Registrant and
PharmaZell GMBH

10.37++ Sumitomo Agreement, dated March 29, 2011, between the

Form 10-K

10.41

February 25, 2021

Registrant and Sumitomo Dainippon Pharma Co., Ltd.

10.38 Amendment No. 1, dated June 8, 2011, to that certain

Form 10-Q

10.1 

May 10, 2018

Sumitomo Agreement, dated March 29, 2011, between the
Registrant and Sumitomo Dainippon Pharma Co., Ltd.

10.39 Amendment No. 2, dated September 16, 2011, to that
certain Sumitomo Agreement, dated March 29, 2011,
between the Registrant and Sumitomo Dainippon Pharma
Co., Ltd.

10.40+ Amendment No. 3, dated February 13, 2018, to that certain
Sumitomo Agreement, dated March 29, 2011, between the
Registrant and Sumitomo Dainippon Pharma Co., Ltd.

Form 10-Q

10.2 

May 10, 2018

Form 10-Q

10.3 

May 10, 2018

10.41

Letter Agreement, dated October 25, 2019, between the
Registrant and Sumitomo Dainippon Pharma Co., Ltd.

Form 10-K

10.41

February 25, 2020

10.42++ Agreement of Lease, dated February 7, 2022, between

Form 8-K

10.1

February 9, 2022

United States Fire Insurance Company as Landlord and the
Registrant as Tenant

21.1*

Subsidiaries of the Registrant

23.1*

Consent of Independent Registered Public Accounting
Firm

24.1*

Power of Attorney (included in signature page to this
Annual Report on Form 10-K)

31.1*

Certification of Principal Executive Officer required by
Rule 13a-14(a) or Rule 15d-14(a)

31.2*

Certification of Principal Financial Officer required by
Rule 13a-14(a) or Rule 15d-14(a)

32.1*(4) Certifications required by Rule 13a-14(b) or Rule 15d-
14(b) and Section 1350 of Chapter 63 of Title 18 of the
United States Code (18 U.S.C. 1350)

104

Table of Contents

101*

The following materials from the Registrant’s Annual
Report on Form 10-K for the year ended December 31,
2021, formatted in Inline XBRL (eXtensible Business
Reporting Language): (i) Consolidated Balance Sheets as
of December 31, 2021 and 2020, (ii) Consolidated
Statements of Operations for the Years Ended December
31, 2021, 2020 and 2019, (iii) Consolidated Statement of
Comprehensive Loss for the Years Ended December 31,
2021, 2020 and 2019, (iv) Consolidated Statements of
Changes in Stockholders’ (Deficit) Equity for the Years
Ended December 31, 2021, 2020 and 2019, (v)
Consolidated Statements of Cash Flows for the Years
Ended December 31, 2021, 2020 and 2019 and (vi) Notes
to Consolidated Financial Statements

104*

Cover Page Interactive Data File (formatted as Inline
XBRL and contained in Exhibit 101)

*

Filed herewith.

+ Confidential treatment has been received with respect to certain portions of this exhibit. Omitted portions have been

filed separately with the Securities and Exchange Commission (“SEC”).

++ Portions of the exhibit have been omitted pursuant to Regulation S-K, Item 601(b)(10)(iv).

#

Indicates a management contract or compensatory plan or arrangement.

† Unless otherwise specified, the File No. is 001-35668.

(1) Registration Statement on Form S-8 filed by the Registrant, Registration No. 333-184810.

(2) Registration Statement on Form S-1 filed by the Registrant, Registration No. 333-217861.

(3) Registration Statement on Form S-1 filed by the Registrant, Registration No. 333-183706.

(4) This certification “accompanies” the Annual Report on Form 10-K to which it relates, is not deemed filed with the
SEC  and  is  not  to  be  incorporated  by  reference  into  any  filing  of  Registrant  under  the  Securities  Act  of  1933,  as
amended, or the Securities Exchange Act of 1934, as amended, (whether made before or after the date of the Annual
Report on Form 10-K), irrespective of any general incorporation language contained in such filing.

Item 16.  Form 10-K Summary

None.

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Table of Contents

SIGNATURES

Pursuant to the requirements of Section 13 or 15(d) of the Securities Exchange Act of 1934, the registrant has duly

caused this report to be signed on its behalf by the undersigned, thereunto duly authorized.

Date: March 2, 2022

    By:/s/ Jerome Durso

INTERCEPT PHARMACEUTICALS, INC.

Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

POWER OF ATTORNEY

KNOW ALL PERSONS BY THESE PRESENTS, that each person whose signature appears below hereby constitutes
and appoints Jerome Durso, Andrew Saik and Rocco Venezia, and each of them, as his or her true and lawful attorneys-in-
fact and agents, with full power of substitution and resubstitution, for him or her, and in his or her name, place and stead, in
any and all capacities, to sign any and all amendments to this Annual Report on Form 10-K, and to file the same, with all
exhibits thereto, and all other documents in connection therewith, with the Securities and Exchange Commission, granting
unto each said attorney-in-fact and agent full power and authority to do and perform each and every act and thing required
or necessary to be done in and about the premises, as fully and to all intents and purposes as the undersigned could do in
person,  and  hereby  ratifying  and  confirming  all  that  said  attorneys-in-fact  and  agents,  or  any  of  them  or  their  or  his
substitute or substitutes, may lawfully do or cause to be done by virtue hereof.

Pursuant  to  the  requirements  of  the  Securities  Exchange  Act  of  1934,  this  report  has  been  signed  below  by  the

following persons on behalf of the registrant and in the capacities indicated on March 2, 2022.

Signature

/s/ Jerome Durso
Jerome Durso

/s/ Andrew Saik
Andrew Saik

/s/ Rocco Venezia
Rocco Venezia

/s/ Paolo Fundarò
Paolo Fundarò

/s/ Srinivas Akkaraju, M.D., Ph.D.
Srinivas Akkaraju, M.D., Ph.D.

/s/ Luca Benatti, Ph.D.
Luca Benatti, Ph.D.

/s/ Daniel Bradbury
Daniel Bradbury

/s/ Keith Gottesdiener, M.D.
Keith Gottesdiener, M.D.

Title

President and Chief Executive Officer and Director
(Principal Executive Officer)

Chief Financial Officer
(Principal Financial Officer)

Senior Vice President, Chief Accounting Officer and Treasurer
(Principal Accounting Officer)

Chairman of the Board of Directors

Director

Director

Director

Director

106

    
Table of Contents

/s/ Nancy Miller-Rich
Nancy Miller-Rich

/s/ Mark Pruzanski, M.D.
Mark Pruzanski, M.D.

/s/ Dagmar Rosa-Bjorkeson
Dagmar Rosa-Bjorkeson

/s/ Gino Santini
Gino Santini

/s/ Glenn Sblendorio
Glenn Sblendorio

Director

Director

Director

Director

Director

107

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

Index to Consolidated Financial Statements

Reports of Independent Registered Public Accounting Firm (KPMG LLP, New York, NY, Auditor Firm ID: 185)
Consolidated Financial Statements:
Consolidated Balance Sheets as of December 31, 2021 and 2020
Consolidated Statements of Operations for the Years Ended December 31, 2021, 2020 and 2019
Consolidated Statements of Comprehensive Loss for the Years Ended December 31, 2021, 2020 and 2019
Consolidated Statements of Changes in Stockholders’ (Deficit) Equity for the Years Ended December 31, 2021, 2020
and 2019
Consolidated Statements of Cash Flows for the Years Ended December 31, 2021, 2020 and 2019
Notes to Consolidated Financial Statements

F-2

F-5
F-6
F-7

F-8
F-9
F-11

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Table of Contents

REPORT OF INDEPENDENT REGISTERED PUBLIC ACCOUNTING FIRM

To the Stockholders and Board of Directors
Intercept Pharmaceuticals, Inc.:

Opinion on the Consolidated Financial Statements

We  have  audited  the  accompanying  consolidated  balance  sheets  of  Intercept  Pharmaceuticals,  Inc.  and  subsidiaries  (the
Company)  as  of  December  31,  2021  and  2020,  the  related  consolidated  statements  of  operations,  comprehensive  loss,
changes  in  stockholders’  (deficit)  equity,  and  cash  flows  for  each  of  the  years  in  the  three-year  period  ended
December  31,  2021,  and  the  related  notes  (collectively,  the  consolidated  financial  statements).  In  our  opinion,  the
consolidated  financial  statements  present  fairly,  in  all  material  respects,  the  financial  position  of  the  Company  as  of
December 31, 2021 and 2020, and the results of its operations and its cash flows for each of the years in the three-year
period ended December 31, 2021, in conformity with U.S. generally accepted accounting principles.

We  also  have  audited,  in  accordance  with  the  standards  of  the  Public  Company  Accounting  Oversight  Board  (United
States)  (PCAOB),  the  Company’s  internal  control  over  financial  reporting  as  of  December  31,  2021,  based  on  criteria
established in Internal Control – Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of the
Treadway Commission, and our report dated March 2, 2022 expressed an unqualified opinion on the effectiveness of the
Company’s internal control over financial reporting.

Basis for Opinion

These  consolidated  financial  statements  are  the  responsibility  of  the  Company’s  management.  Our  responsibility  is  to
express  an  opinion  on  these  consolidated  financial  statements  based  on  our  audits.  We  are  a  public  accounting  firm
registered with the PCAOB and are required to be independent with respect to the Company in accordance with the U.S.
federal  securities  laws  and  the  applicable  rules  and  regulations  of  the  Securities  and  Exchange  Commission  and  the
PCAOB.

We  conducted  our  audits  in  accordance  with  the  standards  of  the  PCAOB.  Those  standards  require  that  we  plan  and
perform the audit to obtain reasonable assurance about whether the consolidated financial statements are free of material
misstatement,  whether  due  to  error  or  fraud.  Our  audits  included  performing  procedures  to  assess  the  risks  of  material
misstatement  of  the  consolidated  financial  statements,  whether  due  to  error  or  fraud,  and  performing  procedures  that
respond  to  those  risks.  Such  procedures  included  examining,  on  a  test  basis,  evidence  regarding  the  amounts  and
disclosures in the consolidated financial statements. Our audits also included evaluating the accounting principles used and
significant  estimates  made  by  management,  as  well  as  evaluating  the  overall  presentation  of  the  consolidated  financial
statements. We believe that our audits provide a reasonable basis for our opinion.

Critical Audit Matter

The critical audit matter communicated below is a matter arising from the current period audit of the consolidated financial
statements that was communicated or required to be communicated to the audit committee and that: (1) relates to accounts
or  disclosures  that  are  material  to  the  consolidated  financial  statements  and  (2)  involved  our  especially  challenging,
subjective, or complex judgments. The communication of a critical audit matter does not alter in any way our opinion on
the consolidated financial statements, taken as a whole, and we are not, by communicating the critical audit matter below,
providing a separate opinion on the critical audit matter or on the accounts or disclosures to which it relates.

Assessing deductions from revenue related to certain rebates and discounts accruals

As  discussed  in  Note  2  to  the  consolidated  financial  statements,  the  Company  records  net  product  revenue  by
deducting rebates and discounts, among other items. The rebates and discounts are related to arrangements with the
Centers  for  Medicare  &  Medicaid  Services  and  other  government  agencies,  and  are  estimated  and  accrued  with  a
corresponding reduction of gross product revenues when revenue is recognized. The Company had $39.8 million and
$10.3 million in rebates and discounts accruals as of December 31, 2021 for a European jurisdiction in which final

F-2

Table of Contents

pricing is subject to ongoing negotiations with the government, and for all other jurisdictions, respectively, which were
recorded in accounts payable, accrued expenses and other liabilities on the consolidated balance sheet.

We identified the assessment of deductions from revenue related to certain rebates and discounts accruals as a critical
audit  matter  because  evaluating  the  Company’s  assumptions  involved  especially  challenging  auditor  judgment,
including  specialized  knowledge  of  the  regulatory  environment  in  a  particular  European  jurisdiction.  Rebates  and
discounts are predominantly estimated based on correspondence with government agencies and historical experience
with actual payments and redemptions.

The following are the primary procedures we performed to address this critical audit matter. We evaluated the design
and tested the operating effectiveness of certain internal controls over the Company’s rebates and discounts accruals
process, including controls related to the significant assumptions used in the Company’s estimation of certain rebates
and  discounts.  We  evaluated  the  Company’s  ability  to  estimate  rebates  and  discounts  by  comparing  the  previously
recorded  accruals  to  the  actual  amounts  that  were  settled  and  ultimately  paid  by  the  Company.  We  assessed  the
Company’s current period estimates by comparing the accrued amounts to historical payments and redemptions. We
also performed sensitivity analyses based on potential changes in certain assumptions and assessed the impact relative
to the Company’s accruals as of December 31, 2021. In addition, we involved professionals with specialized skills and
knowledge  of  the  regulatory  environment  in  the  European  jurisdiction  in  which  final  pricing  is  subject  to  ongoing
negotiations with the government, who assisted in assessing the Company’s assumptions in estimating the rebates and
discounts.

We have served as the Company’s auditor since 2008.

New York, New York
March 2, 2022

/s/ KPMG LLP

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Table of Contents

REPORT OF INDEPENDENT REGISTERED PUBLIC ACCOUNTING FIRM

To the Stockholders and Board of Directors
Intercept Pharmaceuticals, Inc.:

Opinion on Internal Control Over Financial Reporting

We have audited Intercept Pharmaceuticals, Inc. and subsidiaries' (the Company) internal control over financial reporting
as of December 31, 2021, based on criteria established in Internal Control – Integrated Framework (2013) issued by the
Committee  of  Sponsoring  Organizations  of  the  Treadway  Commission.  In  our  opinion,  the  Company  maintained,  in  all
material respects, effective internal control over financial reporting as of December 31, 2021, based on criteria established
in Internal Control – Integrated Framework (2013) issued by the Committee of Sponsoring Organizations of the Treadway
Commission.

We  also  have  audited,  in  accordance  with  the  standards  of  the  Public  Company  Accounting  Oversight  Board  (United
States)  (PCAOB),  the  consolidated  balance  sheets  of  the  Company  as  of  December  31,  2021  and  2020,  the  related
consolidated  statements  of  operations,  comprehensive  loss,  changes  in  stockholders’  (deficit)  equity,  and  cash  flows  for
each of the years in the three-year period ended December 31, 2021, and the related notes (collectively, the consolidated
financial statements), and our report dated March 2, 2022 expressed an unqualified opinion on those consolidated financial
statements.

Basis for Opinion

The Company’s management is responsible for maintaining effective internal control over financial reporting and for its
assessment of the effectiveness of internal control over financial reporting, included in the accompanying Management's
Report on Internal Control Over Financial Reporting. Our responsibility is to express an opinion on the Company’s internal
control over financial reporting based on our audit. We are a public accounting firm registered with the PCAOB and are
required  to  be  independent  with  respect  to  the  Company  in  accordance  with  the  U.S.  federal  securities  laws  and  the
applicable rules and regulations of the Securities and Exchange Commission and the PCAOB.

We conducted our audit in accordance with the standards of the PCAOB. Those standards require that we plan and perform
the audit to obtain reasonable assurance about whether effective internal control over financial reporting was maintained in
all material respects. Our audit of internal control over financial reporting included obtaining an understanding of internal
control over financial reporting, assessing the risk that a material weakness exists, and testing and evaluating the design
and operating effectiveness of internal control based on the assessed risk. Our audit also included performing such other
procedures as we considered necessary in the circumstances. We believe that our audit provides a reasonable basis for our
opinion.

Definition and Limitations of Internal Control Over Financial Reporting

A company’s internal control over financial reporting is a process designed to provide reasonable assurance regarding the
reliability  of  financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles. A company’s internal control over financial reporting includes those policies and
procedures  that  (1)  pertain  to  the  maintenance  of  records  that,  in  reasonable  detail,  accurately  and  fairly  reflect  the
transactions and dispositions of the assets of the company; (2) provide reasonable assurance that transactions are recorded
as necessary to permit preparation of financial statements in accordance with generally accepted accounting principles, and
that receipts and expenditures of the company are being made only in accordance with authorizations of management and
directors of the company; and (3) provide reasonable assurance regarding prevention or timely detection of unauthorized
acquisition, use, or disposition of the company’s assets that could have a material effect on the financial statements.

Because of its inherent limitations, internal control over financial reporting may not prevent or detect misstatements. Also,
projections of any evaluation of effectiveness to future periods are subject to the risk that controls may become inadequate
because of changes in conditions, or that the degree of compliance with the policies or procedures may deteriorate.

New York, New York
March 2, 2022

/s/ KPMG LLP

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Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

Consolidated Balance Sheets

Current assets:

Assets

Cash and cash equivalents
Restricted cash
Investment debt securities, available-for-sale
Accounts receivable, net of allowance for credit losses of $296 and $235,
respectively
Prepaid expenses and other current assets

Total current assets

Fixed assets, net
Inventory
Security deposits
Other assets

Total assets

Current liabilities:

Liabilities and Stockholders’ Deficit

Accounts payable, accrued expenses and other liabilities
Short-term interest payable
Total current liabilities

Long-term liabilities:

Long-term debt
Long-term other liabilities

Total liabilities

Commitments and contingencies (Note 19)
Stockholders’ deficit:

Common stock par value $0.001 per share; 90,000,000 shares authorized;
29,572,953 and 33,015,614 shares issued and outstanding as of December
31, 2021 and December 31, 2020, respectively
Additional paid-in capital
Accumulated other comprehensive loss, net
Accumulated deficit

Total stockholders’ deficit
Total liabilities and stockholders’ deficit

December 31, 

2021

2020

(in thousands, except share and per share
data)

$

$

$

$

$

84,709
9,700
334,980

47,617
25,286
502,292
3,377
8,619
6,616
6,119
527,023

158,216
8,601
166,817

539,782
4,386
710,985

30
2,308,653
(2,873)
(2,489,772)
(183,962)
527,023

$

$

$

$

$

58,151
7,503
411,516

41,549
27,022
545,741
6,326
9,027
7,068
12,327
580,489

171,039
8,037
179,076

560,582
7,684
747,342

33
2,233,937
(2,477)
(2,398,346)
(166,853)
580,489

See accompanying notes to consolidated financial statements.

F-5

    
 
   
  
 
   
  
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
  
 
  
 
  
 
  
 
 
 
 
 
  
 
  
 
 
 
 
 
  
 
  
 
 
 
 
 
 
 
 
 
 
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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Operations

Revenue:

Product revenue, net
Licensing revenue
Total revenue
Operating expenses:

Cost of sales
Selling, general and administrative
Research and development
Restructuring

Total operating expenses
Operating loss

Other income (expense):

Interest expense
Gain on extinguishment of debt
Other income, net

Total other income (expense), net

Net loss
Net loss per common and potential common share:

Basic and diluted

Weighted average common and potential common shares
outstanding:

Basic and diluted

2021

Years Ended December 31, 
2020
(in thousands, except per share data)

2019

363,468
—
363,468

3,100
230,855
185,272
(86)
419,141
(55,673)

(54,419)
16,511
2,155
(35,753)
(91,426)

(2.87)

$

$

312,690
—
312,690

249,570
2,432
252,002

5,322
332,493
191,485
14,630
543,930
(231,240)

(48,054)
—
4,414
(43,640)
(274,880)

(8.34)

$

$

4,212
317,418
242,799
—
564,429
(312,427)

(41,144)
—
8,890
(32,254)
(344,681)

(10.89)

$

$

$

$

$

31,894

32,970

31,654

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Comprehensive Loss

Net loss
Other comprehensive (loss) income:
   Net changes related to available-for-sale investment debt securities:
     Unrealized (losses) gains on investment debt securities
     Reclassification adjustment for realized losses (gains) on investment debt 
securities included in other income, net
   Net unrealized (losses) gains on investment debt securities
     Foreign currency translation gains (losses)
   Other comprehensive (loss) income
Comprehensive loss

2021

Years Ended December 31, 
2020
(in thousands)
$ (91,426) $ (274,880) $ (344,681)

2019

(754)

(202)

1,509

$

15
(739) $
343
(396)

(8)
1,501
(379)
1,122
$ (91,822) $ (276,213) $ (343,559)

(135)
(337) $
(996)
(1,333)

See accompanying notes to consolidated financial statements.

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INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Changes in Stockholders’ (Deficit) Equity

For the Years Ended December 31, 2021, 2020 and 2019 (in thousands)

Common Stock

Paid-in

Comprehensive

Accumulated

Stockholders’

Additional

Other

Total

Accumulated

Shares      Amount    
$
29,694

30

—   —  

Capital
$ 1,800,144
55,982

$

Loss, Net

Deficit

(2,259) $ (1,778,785) $
—  

—  

     (Deficit) Equity
19,130
55,982

Balance - December 31, 2018
Stock-based compensation
Recognition of debt discount on 2026
Convertible Notes
Issuance of common stock from public
and private placement offerings, net of
underwriting fees and issuance costs
Net proceeds from exercise of stock
options
Employee withholding taxes related to
stock-based awards
Other comprehensive income
Net loss
Balance - December 31, 2019
Stock-based compensation
Net proceeds from exercise of stock
options
Employee withholding taxes related to
stock-based awards
Other comprehensive loss
Net loss
Balance - December 31, 2020
Stock-based compensation
Issuance of common stock under equity
plan
Employee withholding taxes related to
stock-based awards
Repurchase of common stock
Extinguishment of allocated costs related
to exchange of convertible notes
Extinguishment of allocated costs related
to repurchase of convertible notes
Bifurcation of conversion option upon
issuance of convertible notes, net of
issuance costs
Issuance of common stock for services
related to exchange of convertible notes
Proceeds from capped call transactions
Other comprehensive loss
Net loss
Balance - December 31, 2021

—

2,880

279

—
—
—
  32,853
—

176

$

—

3

—

—
—
—
33
—

—

85,915

227,257

8,993

(2,158)
—
—
$ 2,176,133
60,850

—

—

—

—

—

—

—
1,115
—

—
—  

(344,681)

$

(1,144) $ (2,123,466) $

—

—

—

—

—

(13)
—   —  
—
33,016

—
33

$

(1,052)

(1,994)

—  
—
$ 2,233,937
33,888

$

392

(83)
(4,522)

—

—

—

—

—
(4)

—

—

—

18

(1,737)
(75,821)

(37,213)

(1,933)

147,458

—
(1,333)
—

—
—  

(274,880)

(2,477) $ (2,398,346) $

—

—

—
—

—

—

—

—

—

—
—

—

—

—

1
770
—
—
—
—
—   —
30
$

29,573

9,999
57
—
—
$ 2,308,653

—
—
(396)

—  

—
—
—
(91,426)

$

(2,873) $ (2,489,772) $

See accompanying notes to consolidated financial statements.

F-8

85,915

227,260

8,993

(2,158)
1,115
(344,681)
51,556
60,850

(1,052)

(1,994)
(1,333)
(274,880)
(166,853)
33,888

18

(1,737)
(75,825)

(37,213)

(1,933)

147,458

10,000
57
(396)
(91,426)
(183,962)

    
    
 
 
 
 
 
 
 
 
Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

Consolidated Statements of Cash Flows

Years Ended December 31, 
2020

2021

2019

Cash flows from operating activities:

Net loss
Adjustments to reconcile net loss to net cash used in operating activities:
Stock-based compensation
(Accretion) amortization of (discount) premium on investment debt securities
Amortization of deferred financing costs
Depreciation
Non-cash operating lease cost
Gain on lease termination
Loss on the disposal of fixed assets
Accretion of debt discount
Gain on extinguishment of debt
Provision for allowance of credit losses, net of write-offs
Changes in operating assets:

Accounts receivable
Prepaid expenses and other current assets
Inventory
Security deposits
Other assets

Changes in operating liabilities:

Accounts payable, accrued expenses and other current liabilities
Operating lease liabilities
Interest payable
Deferred revenue
Long-term other liabilities

Net cash used in operating activities

Cash flows from investing activities:

Purchases of investment debt securities
Sales and maturities of investment debt securities
Purchases of equipment, leasehold improvements, and furniture and fixtures

Net cash provided by (used in) investing activities

Cash flows from financing activities:

Payments for repurchase of common stock
Proceeds from issuance of 2026 Convertible Secured Notes, net of issuance
costs
Proceeds from terminations of capped call options
Payments for repurchases of 2023 Convertible Notes
Proceeds from issuance of 2026 Convertible Notes, net of issuance costs
Proceeds from issuance of common stock, net of issuance costs
Proceeds from exercise of options, net
Payments of employee withholding taxes related to stock-based awards

Net cash provided by (used in) financing activities

Effect of exchange rate changes on cash, cash equivalents and restricted cash
Net increase (decrease) in cash, cash equivalents and restricted cash

Cash, cash equivalents and restricted cash at beginning of period
Cash, cash equivalents and restricted cash at end of period
Supplemental disclosure of non-cash transactions:

F-9

$ (91,426)

$ (274,880)

$ (344,681)

33,888
4,674
2,544
2,978
5,783
—
—
30,787
(16,511)
61

(7,141)
1,476
231
391
—

(4,825)
(7,235)
2,686
—
—
(41,639)

60,850
4,006
2,540
3,118
6,142
—
—
25,964
—
235

(2,646)
(3,075)
(269)
(269)
1,385

55,982
(302)
2,130
3,663
5,388
(1,995)
2,682
21,189
—
—

(12,350)
(5,353)
(1,354)
2,562
(24,665)

13,863
(6,990)
—
—
—
  (170,026)

56,411
(6,767)
562
(2,432)
12,717
  (236,613)

(349,457)
420,580
(397)
70,726

  (330,713)
  497,421
(3,891)
  162,817

  (603,014)
  415,162
(1,136)
  (188,988)

(75,825)

—

—

116,734
57
(38,129)
—
—
18
(1,737)
1,118
(1,450)
28,755
65,654
94,409

$

$

—
—
—
—
—
1,301
(1,994)
(693)
(1,224)
(9,126)
74,780
65,654

—
—
—
223,424
227,260
8,993
(2,158)
  457,519
(386)
31,532
43,248
74,780

$

    
    
    
 
   
   
  
 
 
  
 
  
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
  
 
 
 
 
 
 
 
 
 
 
 
  
 
  
 
 
 
 
 
  
 
  
 
  
 
 
 
 
 
 
 
  
 
  
 
  
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Table of Contents

Right-of-use asset obtained in exchange for new operating lease obligations

Net increase in accrued fixed assets

Reconciliation of cash, cash equivalents and restricted cash included in the
consolidated balance sheets:
Cash and cash equivalents
Restricted cash
Total cash, cash equivalents and restricted cash

$

$

$

$

— $

4,721

— $

368

84,709
9,700
94,409

$

$

58,151
7,503
65,654

$

$

$

$

—

—

70,055
4,725
74,780

Supplemental non-cash disclosure:
Exchange for 2023 and 2026 Convertible Notes
Exchange for 2026 Convertible Secured Notes
Issuance of common stock to financial advisor in connection with convertible
notes exchange
Recognition of conversion option upon issuance of 2026 Convertible Secured
Notes
Extinguishment of conversion options upon exchange and repurchase of 2023
Convertible Notes and exchange of 2026 Convertible Notes

(421,200)
382,400

10,000

150,704
(39,146)

—
—

—

—
—

—
—

—

—
—

See accompanying notes to consolidated financial statements

F-10

Table of Contents

1. Overview of Business

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Intercept  Pharmaceuticals,  Inc.  (the  “Company”)  is  a  biopharmaceutical  company  focused  on  the  development  and
commercialization of novel therapeutics to treat progressive non-viral liver diseases, including primary biliary cholangitis
(“PBC”)  and  nonalcoholic  steatohepatitis  (“NASH”).  The  Company  currently  has  one  marketed  product,  Ocaliva
(obeticholic acid or “OCA”). Founded in 2002 in New York, the Company has operations in the United States, Europe and
Canada.

2. Summary of Significant Accounting Policies

Basis of Presentation and Principles of Consolidation

The Company’s financial statements have been prepared in conformity with accounting principles generally accepted
in  the  United  States  of  America  (“U.S.  GAAP”).  The  consolidated  financial  statements  include  the  accounts  of  the
Company  and  its  wholly  owned  subsidiaries.  All  intercompany  balances  and  transactions  have  been  eliminated  in
consolidation. The Company has no unconsolidated subsidiaries or investments accounted for under the equity method.

Use of Estimates

The preparation of these financial statements in conformity with U.S. GAAP requires management to make estimates
and judgments that affect the reported amounts of assets and liabilities, the disclosure of assets and liabilities at the date of
the  consolidated  financial  statements  and  the  reported  amounts  of  revenues  and  expenses  during  the  reporting  period.
Actual results could differ from these estimates.

Foreign Currency

The Company’s functional and reporting currency is the U.S. dollar. Transactions in foreign currencies are recorded at
the exchange rate prevailing on the date of the transaction. The resulting monetary assets and liabilities are translated into
U.S.  dollars  at  exchange  rates  prevailing  on  the  subsequent  balance  sheet  date.  Revenue  and  expense  components  are
translated to U.S. dollars at weighted-average exchange rates in effect during the period. Foreign currency transaction gains
and  losses  resulting  from  remeasurement  are  recognized  in  Other  income,  net  within  the  consolidated  statements  of
operations.  Gains  and  losses  as  a  result  of  foreign  currency  translation  adjustments  are  recorded  as  a  component  of
Accumulated other comprehensive loss, net in the stockholders’ deficit section of the consolidated balance sheets and as
Foreign currency translation gains (losses) within the accompanying consolidated statements of comprehensive loss.

Cash and Cash Equivalents

The Company considers all highly liquid securities with an original or remaining maturity of three months or less at

acquisition to be cash equivalents.

Restricted Cash

Restricted cash relates to short-term bank guarantees which provide financial assurance that the Company will fulfill
certain customer obligations entered into in the normal course of business. The cash is restricted as to withdrawal or use
while the related bank guarantee in favor of the customer remains outstanding.

Credit Losses

The allowance for credit losses is based on the Company’s assessment of the collectibility of customer accounts. The

Company regularly reviews the allowance by considering factors such as historical experience, the aging of the accounts

F-11

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

receivable balances, credit conditions that may affect a customer’s ability to pay, current and forecast economic conditions
and other relevant factors.

The  following  table  summarizes  the  allowance  for  credit  losses  activity  on  the  Company’s  trade  receivables  for  the

year ended December 31, 2021 (in thousands):

Balance at December 31, 2020
   Provision for credit losses
   Write-offs
Balance at December 31, 2021

$

$

235
99
(38)
296

For available-for-sale investment debt securities in an unrealized loss position, the Company first assesses whether it
intends to sell the security or it is more likely than not that it will be required to sell the security before recovery of its
amortized  cost  basis.  If  either  of  the  criteria  regarding  intent  or  requirement  to  sell  is  met,  the  amortized  cost  basis  is
written down to fair value through income. For any investment debt securities that do not meet the criteria, the Company
evaluates  whether  the  decline  in  fair  value  has  resulted  from  credit  losses  or  other  factors.  Management  considers  the
extent in which the fair value of the security is less than amortized costs, any changes to the rating of the security by a
rating agency, changes in interest rates, and any other adverse factors related to the security. If the assessment indicates a
credit loss, the present value of cash flows expected to be collected are compared to the amortized cost basis of the security.
If the expected present value of cash flows is less than the amortized cost basis, a credit loss exists and an allowance for
credit losses is recorded, limited to the amount that the fair value is below the amortized cost basis. Any impairment not
recorded through an allowance is recognized in Other comprehensive (loss) income.

Changes in the allowance for credit losses are recorded as a provision for (or reversal of) credit loss expense. Losses
are charged against the allowance when management believes the uncollectibility of the security is confirmed or whether
either of the criteria regarding intent or requirement to sell is met.

The Company excludes accrued interest from both the fair value and amortized cost basis in the assessment of credit
losses  on  its  available-for-sale  investment  debt  securities  and  will  instead  elect  to  write-off  any  uncollectible  accrued
interest receivable balances in a timely manner, which is defined by the Company as when interest due becomes 90 days
delinquent.

Investment Debt Securities, Available-For-Sale

Investment debt securities are considered to be available-for-sale and are carried at fair market value. The estimated
fair  value  of  the  available-for-sale  investment  debt  securities  is  determined  based  on  quoted  market  prices  or  rates  for
similar instruments. Unrealized gains and losses, if any, are reported in accumulated other comprehensive income (loss).
The  cost  of  investment  debt  securities  is  adjusted  for  amortization  of  premiums  and  accretion  of  discounts  to  maturity,
which is included in Other income, net within the consolidated statements of operations. Realized gains and losses, interest
and dividends on available-for-sale securities are also included in Other income, net.

Fair Value of Financial Instruments

The carrying amounts of certain financial instruments, including cash and cash equivalents, restricted cash, accounts
receivable, prepaid expenses and other current assets, accounts payable, accrued expenses and other liabilities approximate
fair value due to their short-term maturities.

F-12

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Concentration of Credit Risk

Financial  instruments,  which  potentially  subject  the  Company  to  concentrations  of  credit  risk,  principally  consist  of

cash, cash equivalents, investment debt securities and accounts receivables from customers.

The  Company  currently  invests  its  excess  cash  primarily  in  money  market  funds,  and  high  quality,  marketable  debt
instruments  of  corporations,  financial  institutions  and  government  sponsored  enterprises.  The  Company  has  adopted  an
investment policy that includes guidelines relative to credit quality, diversification and maturities to preserve principal and
liquidity.

On  a  consolidated  basis,  for  the  year  ended  December  31,  2021,  the  Company’s  three  largest  customers  (as  defined
below under “Revenue Recognition”) accounted for 32%, 30% and 12%, of the Company’s net product sales, respectively.
These three customers accounted for 31%, 30% and 14%, of the Company’s net product sales in 2020, and 32%, 31% and
15%, of the Company’s net product sales in 2019, respectively.

On a consolidated basis, the Company’s three largest customers accounted for 21%, 26% and 9% of the December 31,
2021  accounts  receivable  balance  and  31%,  17%  and  10%  of  the  December  31,  2020  accounts  receivable  balance,
respectively.  The  Company  monitors  its  customers’  financial  credit  worthiness  in  order  to  assess  and  respond  to  any
changes in their credit profile.

Accounts Receivable

The Company extends credit to customers based on its evaluation of the customer’s financial condition. The Company
records receivables for all billings when amounts are due under standard terms. Accounts receivable are stated at amounts
due  net  of  applicable  prompt  pay  discounts  and  other  contractual  adjustments  as  well  as  an  allowance  for  doubtful
accounts. The Company will write off accounts receivable when the Company determines that they are uncollectible.

Fixed Assets

Fixed assets are stated at cost, and depreciated over the estimated useful life of the assets. Depreciation is recorded
using  the  straight-line  method  over  the  estimated  useful  lives  of  the  respective  assets,  generally  three  to  seven  years.
Leasehold improvements are amortized over the shorter of the asset’s useful life or the life of the lease term. Expenditures
for maintenance and repairs are charged to expense as incurred. Upon sale or retirement of assets, the cost of the assets
disposed  of  and  the  related  accumulated  depreciation  are  removed  from  the  consolidated  balance  sheets  and  any  related
gains or losses are reflected in the consolidated statements of operations.

Impairment of Long-Lived Assets

Long-lived assets consist of fixed assets and right-of-use (“ROU”) assets. The Company evaluates long-lived assets
for impairment when events and circumstances indicate that the carrying amount of an asset or group of assets may not be
fully  recoverable.  If  indicators  of  impairment  exist,  the  Company  assesses  the  recoverability  of  the  affected  long-lived
assets by determining whether the carrying value of such assets can be recovered through undiscounted future operating
cash flows. If the carrying amount is not recoverable, the Company measures the amount of any impairment by comparing
the carrying value of the asset to the present value of the expected future cash flows associated with the use of the asset.
There have been no impairments of any long-lived or right-of-use assets in the periods presented.

Inventory

Inventories are stated at the lower of cost or estimated realizable value. The Company determines the cost of inventory

using the first-in, first-out (or FIFO) method. The Company capitalizes inventory costs associated with the Company's

F-13

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

product after regulatory approval when, based on management's judgment, future commercialization is considered probable
and  the  future  economic  benefit  is  expected  to  be  realized;  otherwise,  such  costs  are  expensed  as  research  and
development.  The  Company  periodically  analyzes  its  inventory  levels  to  identify  inventory  that  may  expire  prior  to
expected  sale  or  has  a  cost  basis  in  excess  of  its  estimated  realizable  value,  and  writes-down  such  inventories  as
appropriate.  In  addition,  the  Company's  product  is  subject  to  strict  quality  control  and  monitoring  which  the  Company
performs throughout the manufacturing process. If certain batches or units of product no longer meet quality specifications
or  become  obsolete  due  to  expiration,  the  Company  records  a  charge  to  cost  of  sales  to  write  down  such  unmarketable
inventory to zero. No such charges were recorded in the years ended December 31, 2021, 2020 or 2019.

Leases

The Company determines if an arrangement is a lease at inception and records ROU assets and lease liabilities on the
consolidated balance sheets at lease commencement based on the present value of remaining lease payments over the lease
term. The Company only considers payments that are fixed and determinable at the time of commencement.

Operating lease liabilities are recognized based on the present value of the future minimum lease payments discounted
by  the  Company’s  incremental  borrowing  rate.  The  Company  measures  ROU  assets  based  on  the  corresponding  lease
liability adjusted for (i) payments made to the lessor at or before the commencement date, (ii) initial direct costs incurred
and (iii) tenant incentives under the lease. The Company’s lease terms may include options to extend or terminate the lease
when it is reasonably certain that it will exercise that option. Lease expense for minimum lease payments is recognized on
a straight-line basis over the lease term.

The Company has elected the practical expedient to exclude short-term leases from its ROU assets and lease liabilities;
therefore leases with an initial term of 12 months or less are not recorded on the balance sheet. The Company recognizes
lease expense for these leases on a straight-line basis over the lease term. The Company elected the practical expedient not
to separate non-lease components from all leases. As the Company’s leases do not provide an implicit rate, the Company
uses an incremental borrowing rate based on the information available at the lease commencement date in determining the
present  value  of  the  lease  payments.  The  Company’s  incremental  borrowing  rate  is  the  estimated  rate  that  would  be
required to pay for a collateralized borrowing equal to the total lease payment over the lease term. The Company estimates
its incremental borrowing rate based on an analysis of publicly traded debt securities of companies with credit and financial
profiles similar to its own.

For  short-term  leases,  the  Company  does  not  record  ROU  assets  or  lease  liabilities,  and  records  rent  expense  in  its
consolidated  statements  of  operations  on  a  straight-line  basis  over  the  lease  term,  with  the  exception  of  variable  lease
payments, which are expensed as incurred.

Convertible Debt

As  of  December  31,  2021,  the  Company  accounts  for  convertible  debt  in  accordance  with  Financial  Accounting
Standards  Board  (“FASB”)  Accounting  Standards  Codification  Subtopic  470-20,  “Debt  with  Conversion  and  Other
Options”  (“ASC  470-20”).  The  Company  separately  accounts  for  the  liability  (debt)  and  equity  (conversion  option)
components of convertible debt instruments by allocating the proceeds from the issuance. The value assigned to the debt
component is the estimated fair value, as of the issuance date, of a similar debt instrument without the conversion option.
The amount of the equity component (and resulting debt discount) is calculated by deducting the fair value of the liability
component  from  the  principal  amount  of  the  convertible  debt  instrument.  The  resulting  debt  discount  is  amortized  as
additional  non-cash  interest  expense  over  the  expected  life  of  the  notes  utilizing  the  effective  interest  method.  For
additional information, see Note 9 — Long-Term Debt.

F-14

Table of Contents

Revenue Recognition

Product Revenue, Net

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The Company recognizes revenue upon delivery of Ocaliva to its customers. The Company provides the right of return
to its customers for unopened product for a limited time before and after its expiration date. Returns are estimated based on
historical experience and product shelf lives.

The Company has written contracts with each of its customers that have a single performance obligation — to deliver
products  upon  receipt  of  a  customer  order  —  and  these  obligations  are  satisfied  when  delivery  occurs  and  the  customer
receives Ocaliva. The Company evaluates the creditworthiness of each of its customers to determine whether collection is
reasonably assured. The wholesale acquisition cost that the Company charges its customers for Ocaliva is adjusted to arrive
at  our  estimated  net  product  revenues  by  deducting  (i)  estimated  government  rebates  and  discounts  related  to  Medicare,
Medicaid and other government programs, (ii) estimated costs of incentives offered to certain indirect customers including
patients, and (iii) trade allowances, such as invoice discounts for prompt payment and customer fees.

Rebates and Discounts

The Company contracts with the Centers for Medicare & Medicaid Services and other government agencies to make
Ocaliva  available  to  eligible  patients.  As  a  result,  the  Company  estimates  any  rebates  and  discounts  and  deducts  these
estimated amounts from its gross product revenues at the time the revenues are recognized. The Company’s estimates of
rebates  and  discounts  are  based  on  the  government  mandated  discounts,  which  are  statutorily-defined  and  applicable  to
these  government  funded  programs  and  assumptions  developed  using  historical  experience  with  actual  payments  and
redemptions. The Company recorded $10.3 million and $9.5 million in such estimates as of December 31, 2021 and 2020,
respectively, in accounts payable, accrued expenses and other liabilities on the consolidated balance sheets.

The  Company  contracts  with  national  authorities  in  Europe  to  make  Ocaliva  available  to  eligible  patients.  In
jurisdictions  in  which  final  pricing  is  subject  to  ongoing  negotiations  with  the  government,  the  Company  estimates  the
rebate expected to be due and deducts these estimated amounts from its gross product revenues at the time the revenues are
recognized. The Company’s estimates of such liabilities have historically been based on current invoice pricing and total
prior  units  sold  and  assumptions  developed  using  benchmarks  of  Ocaliva  pricing  approved  in  other  relevant  European
jurisdictions and relevant information in the ongoing negotiations, including correspondence with regulators. In December
2021, the Company adjusted its estimate of the cumulative rebate estimated for France based on correspondence received
from the French regulator. The Company recorded $39.8 million and $27.4 million in such estimates as of December 31,
2021 and 2020, respectively, in accounts payable, accrued expenses and other liabilities on the consolidated balance sheets.

Other Incentives

Other  incentives  that  the  Company  offers  to  indirect  customers  include  co-pay  assistance  cards  provided  by  the
Company for PBC patients who reside in states that permit co-pay assistance programs. The Company’s co-pay assistance
program is intended to reduce each participating patient’s portion of the financial responsibility for Ocaliva purchase price
to a specified dollar amount. The Company estimates the amount of co-pay assistance provided to eligible patients based
on  the  terms  of  the  program  when  product  is  dispensed  by  the  specialty  pharmacies  to  the  patients.  These  estimates  are
based  on  redemption  information  provided  by  third-party  claims  processing  organizations.  The  Company  recorded  $1.2
million and $1.3 million in such estimates as of December 31, 2021 and 2020, respectively, in accounts payable, accrued
expenses and other liabilities on the consolidated balance sheets.

F-15

Table of Contents

Trade Allowances

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The Company provides invoice discounts on Ocaliva sales to certain of its customers for prompt payment and records
these discounts as a reduction to gross product revenues. These discounts are based on contractual terms. Trade allowances
are recorded in accounts receivable, net of allowance for credit losses on the consolidated balance sheets.

Research and Development Expenses

Research  and  development  costs  that  do  not  have  alternative  future  use  are  charged  to  expense  as  incurred.  This
includes the cost of conducting clinical trials, compensation and related overhead for employees and consultants involved
in research and development and the cost of the Company’s manufacturing activities to supply ongoing and future clinical
trials  and  preclinical  studies.  For  periods  prior  to  commercial  launch,  all  manufacturing  costs  for  OCA  are  expensed  as
research and development expenses. The Company will continue to incur manufacturing costs for OCA that are charged to
research and development expenses for other indications such as NASH prior to their potential approval.

Stock-based Compensation

The  Company  accounts  for  stock-based  compensation  to  employees,  non-employee  directors  and  non-employees
granted  share-based  payments  for  services  in  accordance  with  ASC  Topic  718,  Compensation  —  Stock  Compensation
(“ASC 718”). The Company estimates the fair value of stock option awards using the Black-Scholes option pricing model
on the date of the grant. Stock options granted to employees generally fully vest over four years and have a term of ten
years. Restricted stock unit awards (“RSUs”) and restricted stock awards (“RSAs”) without a market condition are valued
based on the closing price of the Company’s common stock on the date of the grant. The fair value of time-based stock
options and RSUs is recognized and amortized on a straight-line basis over the requisite service period of the award. The
fair  value  of  awards  with  market  conditions  is  estimated  using  the  Monte  Carlo  simulation  method  and  expense  is
recognized on a straight-line basis over the requisite service period of the award. The Company accounts for all forfeitures
when they occur.

Net Loss Per Share

Basic loss per share is computed by dividing net loss attributable to common stockholders (numerator) by the weighted
average  number  of  common  shares  outstanding  (denominator)  during  the  period.  Potentially  dilutive  common  shares
include the shares of common stock issuable upon the exercise of outstanding stock options and unvested restricted stock
units.  The  Company  accounts  for  the  effect  of  the  Convertible  Notes  on  diluted  net  earnings  per  share  using  the  if-
converted method as they may be settled in cash or shares at the Company’s option. Diluted net loss per share is the same
as basic net loss per share, since the effects of potentially dilutive securities are antidilutive given net losses.

Income Taxes

The Company utilizes the asset and liability method of accounting for income taxes. Under this method, deferred tax
assets and liabilities are determined based on the difference between the financial statement carrying amounts and tax bases
of  assets  and  liabilities  using  enacted  tax  rates  in  effect  for  years  in  which  the  temporary  differences  are  expected  to
reverse.

The  Company  determines  the  need  for  a  valuation  allowance  by  assessing  the  probability  of  realizing  deferred  tax
assets. Judgment is required in making this assessment and to the extent future expectations change, the Company would
have to assess the recoverability of its deferred assets at that time.

The  Company’s  tax  returns  are  subject  to  examination  by  U.S.  Federal,  state,  and  foreign  taxing  jurisdictions.  The

impact of an uncertain tax position taken or expected to be taken on an income tax return must be recognized in the

F-16

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

financial statements at the largest amount that is more likely than not to be sustained. An uncertain income tax position will
not be recognized in the financial statements unless it is more likely than not to be sustained.

Segments

The  Company  operates  in  one  segment  focused  on  the  development  and  commercialization  of  novel  therapeutics  to

treat progressive non-viral liver diseases.

Recently Adopted Accounting Pronouncements

In December 2019, the FASB issued Accounting Standards Update (“ASU”) No. 2019-12, “Income Taxes (Topic 740):
Simplifying the Accounting for Income Taxes (“ASU 2019-12”), which is intended to simplify various aspects related to
accounting  for  income  taxes. ASU  2019-12  removes  certain  exceptions  to  the  general  principles  in  Topic  740  and  also
clarifies and amends existing guidance to improve consistent application. This guidance is effective for fiscal years, and
interim periods within those fiscal years, beginning after December 15, 2020, with early adoption permitted. The Company
adopted  ASU  2019-12  on  January  1,  2021  and  its  adoption  did  not  have  any  material  impact  on  the  Company’s
consolidated financial statements and related disclosures.

In August 2020, the FASB issued ASU No. 2020-06, “Debt—Debt with Conversion and Other Options (Subtopic 470-
20)  and  Derivatives  and  Hedging—Contracts  in  Entity’s  Own  Equity  (Subtopic  815-40):  Accounting  for  Convertible
Instruments and Contracts in an Entity’s Own Equity (“ASU 2020-06”), which simplifies the accounting for convertible
instruments  by  eliminating  the  requirement  to  separately  account  for  embedded  conversion  features  as  an  equity
component in certain circumstances. A convertible debt instrument will be reported as a single liability instrument with no
separate  accounting  for  an  embedded  conversion  feature  unless  separate  accounting  is  required  for  an  embedded
conversion feature as a derivative or under the substantial premium model. The ASU simplifies the diluted earnings per
share calculation by requiring that an entity use the if-converted method and that the effect of potential share settlement be
included  in  diluted  earnings  per  share  calculations.  Further,  the  ASU  requires  enhanced  disclosures  about  convertible
instruments. Either a modified retrospective method of transition or a full retrospective method of transition is permissible
for the adoption of this standard. This guidance is effective for fiscal years, and interim periods within those fiscal years,
beginning  after  December  15,  2021,  with  early  adoption  permitted.  The  Company  adopted  ASU  2020-06  on  January  1,
2022  using  the  modified  retrospective  method.  Consequently,  financial  information  was  not  updated  and  the  disclosures
required under the new standard were not provided for dates and periods before January 1, 2022. Upon adoption at January
1, 2022, the Company made certain adjustments in our consolidated balance sheet which consisted of an increase of $176.3
million  in  Long-term  debt,  a  net  decrease  of  $307.3  million  in  Additional  Paid-in  Capital  and  a  net  decrease  of  $131.0
million in Accumulated Deficit. Additionally, from January 1, 2022, we will no longer incur non-cash interest expense for
the amortization of debt discount related to the previously separated equity component.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

3. Cash, Cash Equivalents and Investments

The following table summarizes the Company’s cash, cash equivalents and investments as of December 31, 2021 and

2020:

Cash and cash equivalents:
Cash and money market funds
Commercial paper

Total cash and cash equivalents

Investment debt securities:
Commercial paper
Corporate debt securities
Municipal bonds
U.S Treasury securities

Total investment debt securities

Total cash, cash equivalents and investment debt
securities

Cash and cash equivalents:
Cash and money market funds

Total cash and cash equivalents

Investment debt securities:
Commercial paper
Corporate debt securities

Total investment debt securities

Total cash, cash equivalents and investment debt
securities

     Amortized Cost

As of December 31, 2021

Allowance
for Credit
Losses

Gross
Unrealized
Gains

(in thousands)

Gross
Unrealized
Losses

     Fair Value

$

$

76,709
8,000
84,709

84,513
232,721
5,028
12,998
335,260

— $
—
—

—  
—  
—

—  

— $
—
—

—  
16
—
—
16

— $
—
—

76,709
8,000
84,709

(49)
(245)
(1)
(1)
(296)

84,464
  232,492
5,027
12,997
  334,980

$

419,969

$

— $

16

$

(296) $ 419,689

     Amortized Cost

As of December 31, 2020

Allowance
for Credit
Losses

Gross
Unrealized
Gains

Gross
Unrealized
Losses

(in thousands)

Fair Value

$

58,151
58,151

$

55,460
355,597
411,057

— $
—

—  
—  
—  

— $
—

— $
—

58,151
58,151

6
529
535

(9)
(67)
(76)

55,457
  356,059
  411,516

$

469,208

$

— $

535

$

(76) $ 469,667

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  aggregate  fair  value  for  the  Company’s  available-for-sale  investment  debt  securities  that  have  been  in  an

unrealized loss position for less than twelve months or twelve months or longer is as follows:

Less than 12 months

Gross
Unrealized

As of December 31, 2021
12 months or longer
(in thousands)

Gross
Unrealized

Total

Gross
Unrealized

     Fair Value      Losses

    Fair Value     Losses

     Fair Value      Losses

Commercial paper
Corporate debt securities
Municipal bonds
U.S Treasury securities
Total

Commercial paper
Corporate debt securities
Total

$ 81,464
196,120
5,027
12,997
$ 295,608

$

$

(49) $ — $ — $ 81,464
196,120
(245)
(1)
5,027
12,997
(1)
(296) $ — $ — $ 295,608

—
—
—

—
—
—

$

$

(49)
(245)
(1)
(1)
(296)

Less than 12 months

Gross
Unrealized

As of December 31, 2020
12 months or longer
(in thousands)

     Gross

Unrealized

Total

     Gross

Unrealized

     Fair Value      Losses

     Fair Value     Losses

     Fair Value      Losses

$ 32,970
  143,076
$ 176,046

$

$

(9) $ — $ — $ 32,970
(67)
—   143,076
(76) $ — $ — $ 176,046

—  

$

$

(9)
(67)
(76)

At  December  31,  2021  and  2020,  the  Company  had  97  and  66  available-for-sale  investment  debt  securities,
respectively  in  an  unrealized  loss  position  without  an  allowance  for  credit  losses.  Unrealized  losses  on  corporate  debt
securities  have  not  been  recognized  into  income  because  the  issuers’  bonds  are  of  high  credit  quality  (rated  A3/A-  or
higher), management does not intend to sell and it is likely that management will not be required to sell the securities prior
to  their  anticipated  recovery  and  the  decline  in  fair  value  is  largely  due  to  market  conditions  and/or  changes  in  interest
rates.  The  issuers  continue  to  make  timely  interest  payments  on  the  bonds.  The  fair  value  is  expected  to  recover  as  the
bonds approach maturity. For the years ended December 31, 2021 and 2020, no allowance was recorded for credit losses.

Accrued  interest  receivable  on  available-for-sale  investment  debt  securities  totaled  $1.3  million  and  $2.5  million  at
December 31, 2021 and December 31, 2020, respectively, is excluded from the estimate of credit losses and is included in
Prepaid expenses and other current assets.

4. Fair Value Measurements

The  carrying  amounts  of  the  Company’s  receivables  and  payables  approximate  their  fair  value  due  to  their  short

maturities.

Accounting principles provide guidance for using fair value to measure assets and liabilities. The guidance includes a

three-level hierarchy of valuation techniques used to measure fair value, defined as follows:

● Unadjusted Quoted Prices — The fair value of an asset or liability is based on unadjusted quoted prices

in active markets for identical assets or liabilities (Level 1).

● Pricing Models with Significant Observable Inputs — The fair value of an asset or liability is based on
information  derived  from  either  an  active  market  quoted  price,  which  may  require  further  adjustment
based on the attributes of the financial asset or liability being measured, or an inactive market transaction
(Level 2).

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

● Pricing  Models  with  Significant  Unobservable  Inputs  —  The  fair  value  of  an  asset  or  liability  is
primarily based on internally derived assumptions surrounding the timing and amount of expected cash
flows for the financial instrument. Therefore, these assumptions are unobservable in either an active or
inactive market (Level 3).

The Company considers an active market as one in which transactions for the asset or liability occur with sufficient
frequency  and  volume  to  provide  pricing  information  on  an  ongoing  basis.  Conversely,  the  Company  views  an  inactive
market as one in which there are few transactions for the asset or liability, the prices are not current, or price quotations
vary  substantially  either  over  time  or  among  market  makers.  Where  appropriate,  non-performance  risk,  or  that  of  a
counterparty, is considered in determining the fair values of liabilities and assets, respectively.

The Company’s cash deposits, money market funds and U.S Treasury securities are classified within Level 1 of the fair
value hierarchy because they are valued using bank balances or quoted market prices from active markets. Investment debt
securities are classified as Level 2 instruments based on market pricing and other observable inputs.

Financial assets carried at fair value are classified in the tables below in one of the three categories described above:

December 31, 2021
Assets
Cash and cash equivalents:

Money market funds
Commercial paper

Available-for-sale investment debt securities:

Commercial paper
Corporate debt securities
Municipal bonds
U.S. Treasury securities

Total financial assets

December 31, 2020
Assets
Cash and cash equivalents:

Money market funds

Available-for-sale investment debt securities:

Commercial paper
Corporate debt securities

Total financial assets

Total

     Level 1      Level 2

     Level 3

Fair Value Measurements Using

(in thousands)

$ 39,287
8,000

$ 39,287
—

$

— $

8,000

84,464
  232,492
5,027
12,997
$ 382,267

84,464
—  
—   232,492
5,027
—
12,997
$ 52,284

$ 329,983

$

$ 15,492

$ 15,492

$

— $

55,457
  356,059
$ 427,008

—  
55,457
—   356,059
$ 411,516

$ 15,492

$

—
—

—
—
—
—
—

—

—
—
—

The gross realized gains and losses on sales of available-for-sale investment debt securities were not material for the

fiscal years ended December 31, 2021, 2020, and 2019.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  aggregate  fair  value  of  all  available-for-sale  investment  debt  securities  (commercial  paper,  corporate  debt

securities, municipal bonds and U.S. Treasury securities), by contractual maturity, are as follows:

Due in one year or less
Due after one year through two years
Total investment debt securities

Fair Value as of December 31, 

2021

2020

(in thousands)

$

$

305,914
29,066
334,980

$

$

328,077
83,439
411,516

Actual  maturities  may  differ  from  contractual  maturities  because  issuers  may  have  the  right  to  call  or  prepay

obligations without call or prepayment penalties.

5. Fixed Assets, Net

Fixed  assets  are  stated  at  cost  and  depreciated  or  amortized  using  the  straight-line  method  based  on  useful  lives  as

follows:

Office equipment and software
Leasehold improvements
Furniture and fixtures
Subtotal

Less: accumulated depreciation

Fixed assets, net

Useful lives
(Years)

3

  Shorter of remaining lease term or useful life

7

December 31, 

2021

2020

(in thousands)

$
5,373
  13,240
4,588
  23,201
  (19,824)
3,377
$

$

$

5,364
13,237
4,602
23,203
(16,877)
6,326

Depreciation expense for the years ended December 31, 2021, 2020 and 2019 was approximately $3.0 million, $3.1

million and $3.7 million, respectively.

6. Inventory

Inventories are stated at the lower of cost or market. Inventories consisted of the following:

December 31,

2021

2020

Work-in-process
Finished goods
Inventory

7. Leases

$

$

$

(in thousands)
7,801
818
8,619

$

8,394
633
9,027

The Company leases various office spaces under non-cancelable operating leases with original lease periods expiring
between  the  first  quarter  in  2022  and  2025.  The  Company  also  enters  into  leases  for  equipment.  A  number  of  the
Company’s leases include one or more options to renew, with renewal terms that can extend the lease term. The exercise of
lease renewal options is typically at the sole discretion of the Company; therefore, all renewals to extend the lease terms
are not included in the ROU assets and lease liabilities as they are not reasonably certain of exercise.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Operating lease assets and liabilities are classified on the consolidated balance sheet as follows:

Leases
Assets
Operating lease assets
Total leased assets

Liabilities
Current
Operating lease liabilities

Noncurrent
Operating lease liabilities
Total operating lease liabilities

Classification

December 31, 2021 December 31, 2020

Other assets

Accounts payable, accrued expenses
and other liabilities

Long-term other liabilities

$
$

$

$

(in thousands)

6,119
6,119

$
$

12,327
12,327

3,042

$

7,248

4,386
7,428

$

7,684
14,932

Operating lease costs for the years ended December 31, 2021, 2020 and 2019, are as follows:

Lease Cost

Classification

Operating lease cost

Short-term lease cost

Variable lease cost

Sublease expense (income)
Net lease cost

Selling, general and administrative
expenses
Selling, general and administrative
expenses
Selling, general and administrative
expenses
Other income, net

2021

Year Ended December 31, 
2020
(in thousands)

2019

$

6,377

$

6,723

$

6,176

2,001

1,042
—
9,420

$

3,688

1,337
(125)
11,623

$

2,203

829
(788)
8,420

$

As of December 31, 2021 and 2020, respectively, the weighted-average remaining term of the Company’s operating
leases  was  2.8  years  and  2.8  years  and  the  weighted-average  discount  rate  used  to  measure  the  present  value  of  the
Company’s operating lease liabilities was 5.9% and 5.0%.

Cash  payments  included  in  the  measurement  of  the  Company’s  operating  lease  liabilities  reported  in  operating  cash
flows  were  $7.7  million,  $7.9  million  and  $7.5  million  for  the  years  ended  December  31,  2021,  2020  and  2019,
respectively. During the year ended December 31, 2020, the Company obtained ROU assets of $4.7 million in exchange for
new operating lease obligations of $6.1 million.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Maturities  of  the  Company’s  operating  lease  liabilities,  which  do  not  include  short-term  leases,  as  of  December  31,

2021 are as follows:

Maturity of Lease Liabilities

2022
2023
2024
2025
2026
Thereafter
Total lease payments
Less: Present value discount
Total operating lease liabilities

Operating leases

(in thousands)

3,381
2,124
1,605
1,033
—
—
8,143
(715)
7,428

$

$

8. Accounts Payable, Accrued Expenses and Other Liabilities

Accounts payable, accrued expenses and other liabilities consisted of the following:

Accounts payable
Accrued employee compensation
Accrued contracted services
Accrued restructuring
Accrued rebates, discounts and other incentives
Operating lease liabilities
Other liabilities
Accounts payable, accrued expenses and other liabilities

Research & Development Tax Credit

2021

December 31, 

(in thousands)

2020

$

$

18,132
24,511
52,296
—
51,283
3,042
8,952
158,216

$

$

24,594
27,154
62,425
2,504
38,172
7,248
8,942
171,039

The Company has benefited from the U.K. Small and Medium-sized Enterprise R&D Tax Credit scheme, or the SME
scheme, under which it can obtain a tax credit of up to 33.4% of eligible research and development expenses incurred by
the Company in the U.K. Eligible expenses generally include employment costs for research staff, consumables, software
and certain internal overhead costs incurred as part of research projects.

The Company has also started to recently benefit from the U.K. Research and Development Expenditure Scheme, or
the RDEC scheme, under which it can obtain a tax credit of 12% of eligible research and development expenses incurred
by  the  Company  in  the  U.K.  The  RDEC  scheme  is  more  restrictive  than  the  SME  scheme,  and  generally  applies  where
qualifying R&D expenditure is not eligible for relief under the SME scheme.

The Company has submitted claims seeking to obtain tax credits for qualifying R&D expenses incurred in the 2015,
2016, 2017, 2018 and 2019 calendar years. As described further in Note 14, the 2017 SME claim was finalized during the
quarter ended June 30, 2021, and therefore the $9.4 million payment received in June 2020, which was previously deferred,
was released into income as a reduction to Research & development expenses.

With  respect  to  the  2018  RDEC  claim,  in  June  2021,  the  Company  received  a  payment  of  $4.2  million  from  Her

Majesty’s Revenue and Customs (“HMRC”), the U.K.’s government tax authority. In October 2021, the Company filed a

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

letter of adjustment and made a cash repayment of $0.2 million to the HMRC due to submission of the amended claim.
Given  the  claim  review  has  not  been  finalized  for  the  2018  year,  the  $4.0  million  net  credit  received,  which  has  been
reduced  by  $0.2  million  due  to  foreign  currency  translation  is  recorded  as  a  deferred  liability  within  Accounts  payable,
accrued expenses and other liabilities.

9. Long-Term Debt

Debt, net of discounts and deferred financing costs, consisted of the following:

2026 Convertible Secured Notes
2026 Convertible Notes
2023 Convertible Notes
Long-term debt, gross

Less: Unamortized debt discounts and fees

Long-term debt, net

December 31, 2021    December 31, 2020

(in thousands)

$

$

500,000
115,349
113,655
729,004
(189,222)
539,782

$

$

-
230,000
460,000
690,000
(129,418)
560,582

The Company has three series of convertible notes outstanding (together, the “Convertible Notes”). All three series are
convertible under certain circumstances into cash, shares of the Company’s common stock, or a combination thereof, at the
Company’s election.

The 2023 Convertible Notes were issued on July 6, 2016, in the amount of $460.0 million principal, at an interest rate
of  3.25%.  The  Company  received  net  proceeds  from  their  sale  of  $447.6  million,  net  of  $12.4  million  in  underwriting
discounts, commissions, and estimated offering expenses.

The 2026 Convertible Notes were issued on May 14, 2019, in the amount of $230.0 million principal, at an interest
rate of 2.00%. The Company received net proceeds from their sale of $223.4 million, net of $6.6 million in underwriting
discounts, commissions, and estimated offering expenses.

On  August  10,  2021,  the  Company  entered  into  privately  negotiated  exchange  and  subscription  agreements  with  a
limited  number  of  existing  “accredited  investors”  and  “qualified  institutional  buyers”  (as  defined  under  Securities  Act
rules)  holding  2023  Convertible  Notes  and  2026  Convertible  Notes  to  (1)  exchange  $306.5  million  principal  of  2023
Convertible Notes for $292.4 million principal of new notes, (2) exchange $114.7 million principal of 2026 Convertible
Notes for $90.0 million principal of new notes, and (3) sell $117.6 million principal of new notes for cash. On August 17,
2021,  these  new  notes  were  issued  as  2026  Convertible  Secured  Notes  in  the  amount  of  $500.0  million  principal,  at  an
interest rate of 3.50%. The Company received cash proceeds from the sale of notes of approximately $116.7 million, net of
$0.9 million in issuance costs. The Company also paid its financial advisor $10.0 million in stock for services rendered, in
the amount of 769,823 shares, based on the closing price of $12.99 per share on August 20, 2021.

Further, on September 9, 2021, the Company entered into privately negotiated agreements with certain holders of 2023
Convertible Notes to repurchase $39.9 million principal for $38.1 million in cash, which purchase closed on September 14,
2021.

Net  of  these  transactions,  as  of  December  31,  2021,  the  Company  has  $729.0  million  in  gross  long-term  debt,  as

shown in the table above.

The approximate fair value of the Convertible Notes was determined as follows using Level 2 inputs based on quoted

market values:

F-24

    
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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

2026 Convertible Secured Notes
2026 Convertible Notes
2023 Convertible Notes

December 31, 2021

December 31, 2020

$
$
$

(in thousands)

543,370
69,492
107,727

$
$
$

-
142,837
363,690

In accordance with Accounting Standards Codification (“ASC”) Subtopic 470-20, “Debt with Conversion and Other
Options” (“ASC 470-20”), the exchange of the 2023 Convertible Notes and 2026 Convertible Notes and repurchase of the
2023 Convertible Notes were all treated as extinguishments of debt. The difference between the consideration attributed to
the  liability  component,  and  its  net  carrying  cost,  resulted  in  a  gain  on  extinguishment.  The  difference  between  the
consideration  attributed  to  the  equity  component,  and  its  net  carrying  cost,  resulted  in  a  reduction  to  additional  paid-in
capital.

Exchange of 2023 Convertible Notes
Exchange of 2026 Convertible Notes
Repurchase of 2023 Convertible Notes
Total

$

$

Gain on extinguishment of debt

Reduction to additional paid-in capital

2,169
13,839
503
16,511

(in thousands)
$

$

14,139
23,074
1,933
39,146

At  issuance,  in  accordance  with  ASC  470-20,  the  Company  used  effective  interest  rates  to  determine  the  liability
components of the Convertible Notes, with the residual as the debt discount, with a corresponding increase to additional
paid-in capital for the equity component of the Convertible Notes. The Company used an effective interest rate of 12.46%,
to  determine  the  liability  component  of  the  2026  Convertible  Secured  Notes,  for  the  purpose  of  initial  recognition,  and
14.62%,  8.94%  and  9.32%  for  the  exchange  of  2026  Convertible  Notes,  exchange  of  2023  Convertible  Notes  and
repurchase of 2023 Convertible Notes, respectively, for the calculation of the fair values of the Company’s extinguished
debt for purposes of determining the gain on extinguishment. This resulted in the initial recognition of $349.3 million as
the  liability  component  and  the  residual  $150.7  million  as  the  debt  discount  for  the  equity  component  of  the  2026
Convertible  Secured  Notes.  The  remaining  2026  Convertible  Notes  and  2023  Convertible  Notes  were  not  subject  to
remeasurement and after giving effect to the reductions in additional paid-in capital, the remaining balances of the equity
components are $62.8 million and $97.1 million, respectively.

Underwriting  discounts,  commissions,  and  estimated  offering  expenses  (both  cash  and  non-cash)  were  allocated  as
debt or equity issuance costs in proportion to the allocation of the liability and equity components of the Convertible Notes,
with debt issuance costs recorded as a deduction from the carrying value of the debt, and equity issuance costs recorded as
an  offset  to  additional  paid-in  capital.  Debt  issuance  costs  of  $7.5  million,  $4.1  million  and  $9.4  million  for  the  2026
Convertible  Secured  Notes,  2026  Convertible  Notes  and  2023  Convertible  Notes,  respectively,  were  recorded  on  the
issuance date and are reflected as a direct deduction from the carrying value of the associated debt liability. Equity issuance
costs of $3.3 million, $2.5 million and $3.0 million for the 2026 Convertible Secured Notes, 2026 Convertible Notes, and
2023 Convertible Notes, respectively were recorded on the issuance date as an offset to additional paid-in capital.

The  debt  discount  and  debt  issuance  costs  will  be  amortized  as  non-cash  interest  expenses  through  the  scheduled

maturity of the Convertible Notes.

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The Note Indentures

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The 2023 Convertible Notes, and the 2026 Convertible Notes, were each issued pursuant to a Base Indenture, dated as
of  July  6,  2016,  between  the  Company  and  U.S.  Bank  National  Association  (“U.S.  Bank”),  as  trustee,  and  a  First
Supplemental Indenture (with respect to the 2023 Convertible Notes) and Second Supplemental Indenture (with respect to
the  2026  Convertible  Notes),  dated  July  6,  2016,  and  May  14,  2019,  respectively,  each  between  the  Company  and  U.S.
Bank as trustee. The 2026 Convertible Secured Notes were issued pursuant to a Base Indenture and a First Supplemental
Indenture,  each  dated  as  of  August  17,  2021,  between  the  Company  and  U.S.  Bank  as  trustee  and  collateral  agent.  In
connection with the issuance of the 2026 Convertible Secured Notes, the Company also entered into a Security Agreement,
dated as of August 17, 2021, with U.S. Bank as collateral agent.

Pursuant to these indentures, the 2023 Convertible Notes and 2026 Convertible Notes are senior unsecured obligations,
and  the  2026  Convertible  Secured  Notes  are  senior  secured  obligations,  of  the  Company.  Each  indenture  provides  for
customary events of default.

Each series of notes bears a fixed rate of interest as identified above, payable semi-annually in arrears:

2026 Convertible Secured Notes
2026 Convertible Notes
2023 Convertible Notes
* Unless earlier repurchased, redeemed, or converted.

First payment date
February 15, 2022
November 15, 2019
January 1, 2017

Semi-annual payment dates

First
February 15
May 15
January 1

Second
August 15
November 15
July 1

Maturity date*
February 15, 2026
May 15, 2026
July 1, 2023

Each  of  the  three  series  of  notes  is  convertible  under  certain  circumstances.  Prior  to  January  1,  2023  (for  the  2023
Convertible Notes), February 15, 2026 (for the 2026 Convertible Notes), and November 15, 2025 (for the 2026 Convertible
Secured Notes), holders may convert their notes only under any of the following circumstances:

(i) During  any  calendar  quarter  commencing  after  the  calendar  quarter  ended  on  September  30,  2016  (for  the
2023  Convertible  Notes),  June  30,  2019  (for  the  2026  Convertible  Notes),  or  December  31,  2021  (for  the
2026 Convertible Secured Notes), if the last reported sale price of the Company’s common stock for at least
20 trading days (whether or not consecutive) during the period of 30 consecutive trading days ending on the
last trading day of the immediately preceding calendar quarter is at least 130% of the applicable conversion
price  (as  defined  in  the  applicable  indenture)  on  each  applicable  trading  day  (the  “Stock  Price  Conversion
Condition”).

(ii) During the five business day period after any five consecutive trading day period in which the trading price
(as defined in the applicable indenture) per $1,000 principal amount for each trading day was less than 98%
of the product of the last reported sale price of the Company’s common stock and the applicable conversion
rate (as defined in the applicable indenture) on each such trading day.

(iii) If the Company calls any or all of the applicable series of notes for redemption, at any time prior to the close

of business on the scheduled trading day immediately preceding the redemption date.

(iv) Upon the occurrence of specified corporate events.

After  those  dates,  holders  may  convert  their  notes,  regardless  of  the  foregoing  circumstances,  at  any  time  until

immediately preceding the applicable maturity date.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Upon conversion of notes, the Company will pay or deliver cash, shares of common stock (or cash in lieu of fractional

shares), or a combination of cash and common stock, at the Company’s election.

The  initial  conversion  rates  of  the  Convertible  Notes  per  $1,000  principal  amount,  and  the  approximate  conversion

price, are as follows:

2026 Convertible Secured Notes
2026 Convertible Notes
2023 Convertible Notes

Initial conversion rate
47.7612
9.2123
5.0358

Approximate conversion price
$20.94
$108.55
$198.58

These conversion rates are subject to adjustment upon occurrence of certain events but will not be adjusted for accrued
and  unpaid  interest.  Also,  if  certain  specified  events  occur,  the  conversion  rate  will  be  increased  for  notes  converted  in
connection with such events.

The Convertible Notes are redeemable by the Company in certain circumstances starting July 6, 2021 (for the 2023
Convertible  Notes),  May  20,  2023  (for  the  2026  Convertible  Notes),  and  February  20,  2024  (for  the  2026  Convertible
Secured Notes). After such dates, the Company may redeem for cash all or any part of the applicable Convertible Notes, at
its option, if the last reported sale price of the common stock has been at least 130% of the applicable conversion price then
in effect for at least 20 trading days (whether or not consecutive) during any 30 consecutive trading day period ending on
and including the trading day immediately preceding the date of the applicable notice of redemption. The redemption price
is  equal  to  100%  of  the  principal  amount  redeemed,  plus  accrued  and  unpaid  interest  to  (but  excluding)  the  redemption
date.

No sinking fund is provided for any of the Convertible Notes.

If the Company undergoes a fundamental change (as defined in the applicable indenture), noteholders may require the
Company to repurchase for cash all or any portion of their notes at a fundamental change repurchase price equal to 100%
of the principal amount of the notes to be repurchased, plus accrued and unpaid interest to (but excluding) the fundamental
change repurchase date.

Upon  the  occurrence  of  certain  corporate  events  (i.e.,  a  “make-whole  fundamental  change”,  as  defined  in  the
applicable  indenture),  the  Company  will,  under  certain  circumstances,  increase  the  conversion  rate  for  holders  of  the
Convertible  Notes  who  elect  to  convert  in  connection  with  such  corporate  events.  In  addition,  with  respect  to  the  2026
Convertible Secured Notes, (1) if the Company elects to redeem all or part of such notes and provides notice of redemption
to the holders or (2) if the Stock Price Conversion Condition is satisfied with respect to any calendar quarter commencing
after the quarter ended September 30, 2022, the Company will, under certain circumstances, increase the conversion rate
for  holders  who  elect  to  convert  (1)  during  the  related  redemption  period,  or  (2)  in  connection  with  such  Stock  Price
Conversion Condition. Upon a Company redemption of the 2026 Convertible Secured Notes, holders of notes called for
redemption  may  be  eligible  to  receive  a  make-whole  premium.  The  Company,  at  its  option,  will  satisfy  the  conversion
obligation through cash, shares of common stock, or a combination of cash and common stock. The right to redeem the
2026 Convertible Secured Notes requires the Company to specify a date of redemption no earlier than 60 days and no later
than 90 days after the notice of redemption is sent. If a holder elects to convert its 2026 Convertible Secured Notes prior to
the effective date of a make-whole fundamental change or the date of the redemption notice, then it is not entitled to the
increased conversion rate in connection with such make-whole fundamental change or redemption.

Upon  certain  events  of  default  occurring  and  continuing,  either  the  indenture  trustee  or  holders  of  at  least  25%  in
aggregate principal amount of a series of notes then outstanding may declare the entire principal amount of that series of
notes,  and  accrued  interest,  if  any,  to  be  immediately  due  and  payable.  Upon  events  of  default  involving  specified
bankruptcy events involving the Company, the Convertible Notes are due and payable immediately.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The 2026 Convertible Secured Notes indenture and security agreement include (1) customary covenants, (2) guarantor
provisions,  and  (3)  collateral  provisions.  The  2026  Convertible  Secured  Notes  may  become  guaranteed  in  the  future  by
subsidiaries of the Company that meet certain threshold requirements, with the 2026 Convertible Secured Notes becoming
senior obligations of such guarantor. The 2026 Convertible Secured Notes are secured by a first priority security interest in
substantially all assets of the Company, and of any guarantors, subject to certain exceptions.

The Capped Call Transactions

On June 30, 2016, in connection with the pricing of the 2023 Convertible Notes, the Company entered into privately-
negotiated  capped  call  agreements  (the  “Base  Capped  Calls”)  with  each  of  Royal  Bank  of  Canada,  UBS  AG,  London
Branch,  and  Credit  Suisse  Capital  LLC.  On  July  1,  2016,  in  connection  with  the  underwriters’  exercise  of  their  over-
allotment option in full, the Company entered into additional capped call agreements (the “Additional Capped Calls” and,
together with the Base Capped Calls, the “Capped Calls”) with same counterparties.

The Capped Calls are considered to be instruments indexed to the Company’s own shares and met the criteria to be

classified within equity. Therefore, they are not remeasured.

In  August  2021,  in  connection  with  the  exchange  of  2023  Convertible  Notes,  of  the  460,000  Capped  Call  options
outstanding  (400,000  Base  Capped  Call  options  and  60,000  Additional  Capped  Call  Options),  306,486  options  were
terminated (246,486 Base Capped Call options and 60,000 Additional Capped Call options), equivalent to approximately
1.5 million shares.

In September 2021, in connection with the additional repurchase of $39.9 million of 2023 Convertible Notes, 39,859
additional Capped Call options were terminated, equivalent to approximately 0.2 million shares, with 113,655 Base Capped
Call options remaining, equivalent to approximately 0.6 million shares.

Upon  settlement  of  each  termination,  the  Company  received  an  immaterial  amount  in  cash  proceeds,  which  was

recorded as an increase to additional paid-in capital.

Interest Expense on Convertible Notes

The table summarizes the total interest expense recognized in the periods presented:

Contractual interest expense
Accretion of debt discount
Amortization of debt issuance costs
Total interest expense

2021

Years Ended December 31, 
2020
(in thousands)

2019

$

$

21,088
30,787
2,544
54,419

$

$

19,550
25,964
2,540
48,054

$

$

17,825
21,189
2,130
41,144

Accrued interest on the Convertible Notes was approximately $8.6 million and $8.1 million as of December 31, 2021
and  December  31,  2020,  respectively.  After  giving  effect  to  the  exchange  and  repurchase,  the  Company’s  total  recorded
debt issuance costs are $14.0 million, which are being amortized using the effective interest method through the date of
maturity.  As  of  December  31,  2021,  and  2020,  $10.3  million  and  $10.7  million,  respectively,  of  debt  issuance  costs  are
unamortized on the consolidated balance sheets in Long-term debt. Cash payments for interest were $18.4 million, $19.6
million and $17.3 million for the years ended December 31, 2021, 2020 and 2019, respectively.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

10. Stockholders’ Equity and Preferred Stock

Common Stock

As  of  December  31,  2021  and  2020,  the  Company  had  90,000,000  authorized  shares  of  common  stock,  par  value

$0.001 per share, respectively.

In connection with the note exchange transactions described in Note 9, on August 11, 2021, the Company completed a
repurchase  of  4,521,502  shares  of  its  common  stock  for  an  aggregate  cash  cost  of  $75.8  million.  The  Company
subsequently  retired  the  shares  of  common  stock.  The  Company’s  common  stock  is  reduced  by  an  amount  equal  to  the
number of shares repurchased multiplied by the par value of such shares. The excess amount that is repurchased over its
par value is allocated as a reduction to additional paid-in capital. The Company also issued 769,823 shares to its financial
advisor  for  services  rendered,  equivalent  to  $10.0  million.  The  financial  advisory  fee  was  allocated  as  debt  or  equity
issuance costs in proportion to the allocation of the liability and equity components of the 2026 Convertible Secured Notes.

Dividends

Subject to preferences that may be applicable to any outstanding shares of preferred stock, holders of common stock
are  entitled  to  receive  ratably  such  dividends,  if  any,  as  may  be  declared  from  time  to  time  by  the  Company’s  board  of
directors out of funds legally available for dividend payments. The Company has never declared or paid any cash dividends
on its common stock, and does not anticipate paying any cash dividends on its common stock in the foreseeable future. As
part of the agreements for the 2026 Convertible Secured Notes, the Company is restricted from dividend payments. The
Company  intends  to  retain  all  available  funds  and  any  future  earnings  to  fund  the  development  and  expansion  of  its
business. Any future determination to pay dividends will be at the discretion of the board of directors and will depend upon
a  number  of  factors,  including  the  results  of  operations,  financial  condition,  future  prospects,  contractual  restrictions,
restrictions imposed by applicable law and other factors the board of directors deems relevant.

Voting

Holders of common stock are entitled to one vote for each share held with respect to all matters submitted to a vote of

the stockholders and do not have cumulative voting rights.

Preferred Stock

As  of  December  31,  2021  and  2020,  the  Company  had  5,000,000  authorized  shares  of  preferred  stock,  par  value

$0.001 per share, of which none are issued.

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11. Product Revenue, Net

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  Company  recognized  net  sales  of  Ocaliva  of  $363.5  million,  $312.7  million  and  $249.6  million  for  the  years

ended December 31, 2021, 2020 and 2019, respectively.

The table below summarizes consolidated product revenue, net by region:

2021

Years Ended December 31, 
2020
(in thousands)

2019

$

$

260,750
102,718
363,468

$

$

233,970
78,720
312,690

$

$

187,436
62,134
249,570

Product revenue, net:

U.S.
ex-U.S.

Total product revenue, net

12. License Agreement

Sumitomo Dainippon Pharma Co., Ltd.

In  March  2011,  the  Company  entered  into  an  exclusive  license  agreement  (the  “Sumitomo  Agreement”)  with
Sumitomo Dainippon Pharma Co., Ltd. (“Sumitomo Dainippon”), pursuant to which the Company granted to Sumitomo
Dainippon an exclusive license to research, develop and commercialize OCA for the treatment of PBC and NASH in Japan
and China (excluding Taiwan) and an option to research, develop and commercialize OCA in certain countries outside of
such territories (the “Country Option”). The Company received an upfront payment from Sumitomo Dainippon of $15.0
million under the terms of the Sumitomo Agreement. In October 2019, the Company and Sumitomo Dainippon mutually
agreed to terminate with immediate effect the Sumitomo Agreement. In connection with the termination of the Sumitomo
Agreement, Sumitomo Dainippon agreed to return to the Company the rights to develop and commercialize OCA in China
and  the  Company  agreed  to  forego  any  further  milestone  or  royalty  payments  relating  to  the  development  and
commercialization of OCA in China. No payment was due from the Company to Sumitomo Dainippon as a result of the
termination of the Sumitomo Agreement.

The Company recognized licensing revenue of approximately $0.0 million, $0.0 million and $2.4 million for the years

ended December 31, 2021, 2020, and 2019, respectively, under the Sumitomo Agreement.

13. Stock Compensation

The  Company’s  2012  Equity  Incentive  Plan  (“2012  Plan”)  became  effective  upon  the  pricing  of  its  initial  public
offering  in  October  2012  (the  “IPO”).  At  the  same  time,  the  Company’s  2003  Stock  Incentive  Plan  (“2003  Plan”)  was
terminated and 555,843 shares available under the 2003 Plan were added to the 2012 Plan.

On January 1, 2021, the number of shares available for issuance under the 2012 Plan increased by 1,211,533 as a result

of the automatic increase provisions thereof.

The Company launched on August 16, 2021, and closed on September 17, 2021, an offer to exchange eligible out-of-
the-money  employee  stock  options  for  a  lesser  number  of  new  options  with  at-the-money  strike  prices  (the  “Option
Exchange”).  Following  expiration  of  the  Option  Exchange,  out  of  703,967  eligible  options,  the  Company  accepted  for
exchange 612,080 original options, with a weighted average exercise price of $99.79 and exchanged them for 338,848 new
options,  granted  effective  September  20,  2021,  with  a  strike  price  of  $15.18,  the  closing  stock  price  on  that  day.  The
original options have been cancelled. Original options that had already vested were exchanged for new options vesting one
year from the new grant date, subject to the employee’s continued employment. Original options that had not already

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

vested were exchanged for new options vesting two years from the new grant date, subject to the employee’s continued
employment. New options will expire after 6.5 years. On the date of modification, incremental compensation cost related
to the difference in the fair values of the original options and the new options of $1.0 million was measured and will be
recognized over the revised requisite service period.

The estimated fair value of the stock options granted in the year ended December 31, 2021 (including but not limited
to  the  exchanged  options)  was  determined  utilizing  a  Black-Scholes  option-pricing  model  at  the  date  of  grant.  The  fair
value  of  the  RSUs  granted  in  the  year  ended  December  31,  2021  was  determined  utilizing  the  closing  price  of  the
Company’s common stock on the date of grant. The fair value of the performance restricted stock units (“PRSUs”) granted
in  the  year  ended  December  31,  2021  was  determined  utilizing  the  Monte  Carlo  simulation  method.  The  Company
accounts for all forfeitures when they occur. Ultimately, the actual expense recognized over the vesting period will be for
only those shares that vest and are not forfeited.

There  were  approximately  3.6  million  and  3.3  million  shares  available  for  grant  remaining  under  the  2012  Plan  at

December 31, 2021 and 2020, respectively.

Stock Options and Performance-Based Stock Options

The  Company’s  outstanding  option  activity  for  the  period  from  December  31,  2020  through  December  31,  2021  is

summarized as follows:

Outstanding at December 31, 2020
Granted
Exercised
Exchanged, net
Cancelled/forfeited
Expired
Outstanding at December 31, 2021
Expected to vest
Exercisable

Number
of Options
(in thousands)

Weighted
Average

Weighted
Average
Remaining
Contractual

Exercise Price      Term (years)     

Aggregate
Intrinsic Value
(in thousands)

2,199
1,305
(2)
(273)
(517)
(460)
2,252
1,320
932

$
$
$
$
$
$
$
$
$

96.92  
26.00  
8.67  
—
53.96  
108.77  
50.28  
26.21  
84.35  

$
6.9
— $
— $
— $
— $
— $
$
7.2
$
8.5
$
5.5

146
—
—
—
—
—
408
408
—

The  aggregate  intrinsic  value  of  options  is  calculated  as  the  difference  between  the  exercise  price  of  the  underlying
options and the deemed fair value of the Company’s common stock for those options that had exercise prices lower than
the deemed fair value of the Company’s common stock. The weighted-average grant date fair value of options granted in
the years ended December 31, 2021, 2020 and 2019 was $26.00, $52.48 and $74.78 per option, respectively. The aggregate
intrinsic value of stock options exercised during the years ended December 31, 2021, 2020 and 2019 was $0.0 million, $0.9
million and $10.2 million, respectively. As of December 31, 2021, the total compensation cost related to non-vested option
awards not yet recognized is approximately $23.8 million with a weighted average remaining vesting period of 1.33 years.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  Company  estimated  the  fair  value  of  stock  options  granted  in  the  periods  presented  utilizing  a  Black-Scholes

option-pricing model utilizing the following assumptions:

Volatility
Expected term (in years)
Risk-free rate
Expected dividend yield

Years Ended December 31, 
2020
  65.2 - 69.3% 61.9 - 87.1 % 86.9 - 89.9 %

2021

2019

3.8 - 6.0  
0.4 - 1.2 %  
— %  

5.5 - 6.0  
0.2 - 1.7 %
— %

5.5 - 6.0
1.4 - 2.9 %
— %

Restricted Stock Units and Awards & Performance-Based Restricted Stock Units and Awards

The following table summarizes the aggregate RSU, RSA and PRSU activity for the year ended December 31, 2021:

Non-vested awards at December 31, 2020

Granted
Vested
Forfeited

Non-vested awards at December 31, 2021

Number of
Awards
(in thousands)
$
799
1,006
$
(379) $
(458) $
968
$

Weighted
Average Grant Date
Fair Value

72.43
27.49
54.29
60.03
39.58

For the years ended December 31, 2021, 2020 and 2019, the weighted-average grant date fair value of RSUs, RSAs,
PRSUs granted was $27.49, $74.68 and $107.29, respectively. The total fair value of RSUs, RSAs and PRSUs that vested
during  the  years  ended  December  31,  2021,  2020  and  2019  was  $20.6  million,  $30.7  million  and  $29.8  million,
respectively. As of December 31, 2021, there was $32.0 million of unrecognized compensation expense related to unvested
RSUs, RSAs and PRSUs, which is expected to be recognized over a weighted average period of 1.55 years.

During the years ended December 31, 2021, 2020 and 2019, the Company granted a total of 176,794 (34,000 forfeited
due to termination), 64,900 and 57,800 PRSUs to certain of the Company’s executive officers. The performance criterion
for such PRSUs is based on the Total Shareholder Return (“TSR”) of the Company’s common stock relative to the TSR of
the  companies  comprising  the  S&P  Biotechnology  Select  Industry  Index  (the  “TSR  Peer  Group”)  over  a  3-year
performance period and is accounted for as a market condition under ASC 718. The TSR for the Company or a member of
the  TSR  Peer  Group  is  calculated  by  dividing  (a)  the  difference  of  the  ending  average  stock  price  minus  the  beginning
average stock price by (b) the beginning average stock price. The beginning average stock price equals the average closing
stock  price  over  the  one  calendar  month  period  prior  to  the  beginning  of  the  performance  period,  after  adjusting  for
dividends,  as  applicable.  The  ending  average  stock  price  equals  the  average  closing  price  over  the  one  calendar  month
period  ending  on  the  last  day  of  the  performance  period,  after  adjusting  for  dividends,  as  applicable.  The  Company’s
relative TSR is then used to calculate the payout percentage, which may range from zero percent (0%) to one hundred and
fifty percent (150%) of the target award. The Company utilized a Monte Carlo Simulation to determine the grant date fair
value of such PRSUs. The Company recorded approximately $0.8 million (net of forfeitures), $8.0 million (of which $2.9
million related to modifications) and $4.0 million of stock-based compensation related to such PRSUs and PRSAs during
the years ended December 31, 2021, 2020 and 2019, respectively.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

Stock-based compensation expense has been reported in the Company’s statements of operations as follows:

Selling, general and administrative
Research and development
Restructuring
Total stock-based compensation

14. Research and Development Tax Credit

$

$

Years Ended December 31, 
2020
(in thousands)
$

$

45,985
12,824
2,041
60,850

$

$

2021

27,938
5,946
4
33,888

2019

43,170
12,812
—
55,982

The Company has benefited from the U.K. Small and Medium-sized Enterprise R&D Tax Credit scheme, or the SME
scheme, under which it can obtain a tax credit of up to 33.4% of eligible research and development expenses incurred by
the Company in the U.K. Eligible expenses generally include employment costs for research staff, consumables, software
and certain internal overhead costs incurred as part of research projects.

The Company submitted claims seeking to obtain tax credits for qualifying R&D expenses incurred in the years ended
December 31, 2015, 2016 and 2017. In September 2019, the Company received a partial payment of $10.5 million from
HMRC. In April 2020, the Company received the remaining payment for the 2015 and 2016 claim years of $11.3 million.
In June 2020, the Company received a payment of $9.4 million from HMRC for the 2017 claim year.

The  claim  for  2015  and  2016  was  finalized  and  approved  in  the  quarter  ended  June  30,  2020,  at  which  time  the
Company  recorded  the  U.K.  research  and  development  tax  credit  payments  received  of  $22.0  million  as  a  reduction  of
research and development expense in the consolidated statements of operations.

The  claim  for  2017  was  finalized  and  approved  in  the  quarter  ended  June  30,  2021,  at  which  time  the  Company
recorded the U.K. research and development tax credit payments received of $10.7 million as a reduction of research and
development expense in the condensed consolidated statements of operations.

15. Employee Benefit Plans

The Company maintains a defined contribution plan, which is qualified under section 401(k) of the Internal Revenue
Code for U.S. employees. Employees may make contributions by withholding a percentage of their salary up to the Internal
Revenue Service annual limit of $19,500 and $26,000 in 2021 for employees under 50 years old and employees 50 years
old or over, respectively. The Company’s matching contribution vests over four years. The Company made payments of
approximately $3.0 million, $2.2 million and $1.4 million in matching contributions during the years ended December 31,
2021, 2020 and 2019, respectively.

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INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

16. Restructuring Expenses

On August 31, 2020, the Company adopted a plan to reduce its workforce in light of the previously announced receipt
of  a  complete  response  letter  from  the  U.S.  Food  and  Drug  Administration  (the  “FDA”)  with  respect  to  its  New  Drug
Application for OCA for the treatment of liver fibrosis due to NASH (the “2020 Workforce Plan”). The 2020 Workforce
Plan  sought  to  streamline  the  Company’s  operations  and  reduce  operating  expenses,  while  maintaining  the  critical
resources  needed  to  continue  to  support  the  NASH  and  PBC  clinical  programs,  pursue  the  approval  of  OCA  for  the
treatment of liver fibrosis due to NASH and support the Company’s successful PBC business. The 2020 Workforce Plan
resulted in a workforce reduction of approximately 25%, or approximately 170 employees. The 2020 Workforce Plan was
implemented  during  the  third  quarter  of  2020,  immediately  after  its  announcement,  and  completed  during  2021.  In  the
years ended December 31, 2021 and 2020, the Company recorded a benefit of $0.1 million and charges of $14.6 million,
which were primarily related to a reversal of unclaimed other related termination benefits and severance costs and other
related termination benefits incurred in conjunction with the 2020 Workforce Plan, respectively.

The  following  table  reflects  total  (benefits)/expenses  related  to  restructuring  activities  recognized  within  the

consolidated statements of operations as restructuring costs:

Employee compensation costs
Equity compensation costs
Total restructuring costs

2021

Year Ended December 31, 

2020

(in thousands)

2019

$

$

(90) 
4
(86)

$

$

12,589
2,041
14,630

$

$

—
—
—

The total cumulative restructuring costs incurred under the 2020 Workforce Plan were $14.5 million. In the year ended
December 31, 2021, the Company recorded an immaterial amount in non-cash stock-based compensation expense and $2.0
million  in  the  year  ended  December  31,  2020,  in  association  with  the  acceleration  of  the  vesting  of  certain  options  and
RSUs held by terminated employees.

The following table displays a rollforward of the changes to the accrued balances as of December 31, 2021:

Accrued balance at December 31, 2020
Charges incurred
Cash payments made
Other reserve adjustments
Accrued balance at December 31, 2021

Severance and Related Costs

(in thousands)

2,504
180
(2,104)
(580)
—

$

$

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Table of Contents

17. Income Taxes

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The  components  of  loss  before  income  taxes  for  the  years  ended  December  31,  2021,  2020  and  2019  includes  the

following:

United States
Foreign
Total

2021

Years Ended December 31, 
2020
(in thousands)
$ (46,450) $ (126,351) $ (95,708)
(248,973)
  (148,529)
$ (91,426) $ (274,880) $ (344,681)

(44,976)

2019

Income tax expense (benefit) differed from the amounts computed by applying the statutory U.S. Federal income tax

rate of 21% to loss before income taxes as a result of the following:

Computed "expected" tax benefit
State taxes, net of U.S. Federal benefit
U.S. Federal tax credits
U.S. Federal valuation allowance
Stock-based compensation
Officer compensation
Foreign valuation allowance
Foreign tax rate differences
Other
Total

F-35

2019

2021

Years Ended December 31, 
2020
(in thousands)
$ (19,199) $ (57,725) $ (72,383)
—
—
14,786
4,609
508
19,349
32,936
195
—

—
(4,988)
3,151
10,012
496
82,743
(73,298)
1,083

—
(5,787)
26,279
8,098
437
43,414
(12,223)
(2,493)

— $

— $

$

    
    
    
 
 
    
    
    
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

The tax effects of temporary differences that give rise to the deferred tax assets and liabilities at December 31, 2021

and 2020 are presented below:

Deferred tax assets:

U.S. and state net operating loss and other carryforwards
Foreign net operating loss
Stock compensation
Accrued compensation
Accrued expense
Intangible property
Interest limitation
Other

Deferred tax assets before valuation allowance
Valuation allowance
Total deferred tax assets
Deferred tax liabilities:
Convertible Notes

Total deferred tax liabilities
Net deferred tax asset (liability)

Net Operating Loss and other carryforwards

December 31, 

2021

2020

(in thousands)

$

$

174,890
315,876
11,652
4,504
14,890
1,780
10,690
2,030
536,312
(492,239)
44,073

(44,073)
(44,073)

$

— $

178,007
239,607
15,675
5,042
11,143
1,945
9,419
1,749
462,587
(436,476)
26,111

(26,111)
(26,111)
—

As of December 31, 2021, and 2020, the Company had net operating loss carryforwards (“NOLs”) for U.S. Federal
income  tax  purposes  of  $669.7  million  and  $709.4  million,  respectively,  and  other  carryforwards  of  $20.3  million  and
$13.7 million, respectively. The enactment of the Tax Cuts and Jobs Act (“TCJA”) modified the ability of companies to
utilize  NOLs  arising  in  tax  years  beginning  on  or  after  January  1,  2018  by  providing  that  such  NOLs  may  be  carried-
forward indefinitely and used to offset up to 80 percent of taxable income in any given future year. Existing NOLs that
arose  in  tax  years  beginning  prior  to  January  1,  2018  were  not  affected  by  the  TCJA  and  are  generally  eligible  to  be
carried-forward for up to 20 years and used to fully offset taxable income in future years. If not utilized, the Company’s
pre-2018  NOLs  and  other  carryforwards  will  expire  for  U.S.  Federal  income  tax  purposes  between  2024  and  2037.  The
Company also has certain state NOLs in varying amounts depending on the different state tax laws.

As of December 31, 2021, and 2020, the Company had NOLs for foreign income tax purposes of $1.3 billion and $1.2
billion, respectively. Of our $1.3 billion of foreign tax loss carryforwards, approximately $1.2 billion are related to the UK
jurisdiction and may be carried forward indefinitely and the remainder will expire during the next 16 years.

In addition, the Company’s ability to utilize its NOLs may be limited under Section 382 of the Internal Revenue Code
or applicable state and foreign tax law. The Section 382 limitations apply if an “ownership change” occurs. Generally, an
ownership change occurs when certain shareholders increase their aggregate ownership by more than 50 percentage points
over their lowest ownership percentage in a testing period (typically three years). The Company has evaluated whether one
or more ownership changes under Section 382 have occurred since its inception and has determined that there have been at
least  two  such  changes.  Although  the  Company  believes  that  these  ownership  changes  have  not  resulted  in  material
limitations  on  its  ability  to  use  these  NOLs,  its  ability  to  utilize  these  NOLs  may  be  limited  due  to  future  ownership
changes or for other reasons. As a result, the Company may not be able to take full advantage of its carryforwards for U.S.
Federal, state, and foreign tax purposes.

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Table of Contents

Valuation Allowance

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

At December 31, 2021 and 2020, the Company maintained a full valuation allowance on its deferred tax assets since it
has  not  yet  achieved  sustained  profitable  operations.  As  a  result,  the  Company  has  not  recorded  any  income  tax  benefit
since its inception. In 2021, the valuation allowance for deferred tax assets increased by approximately $55.8 million. This
includes  an  increase  of  $3.2  million,  decrease  of  $0.5  million  and  increase  of  $82.6  million  for  U.S.  Federal,  state  and
foreign  tax,  respectively,  and  a  decrease  of  $29.5  million  to  equity.  The  increase  in  the  foreign  valuation  allowance
primarily relates to the impact of the UK tax rate which is set to increase from 19% to 25% with effect from April 1, 2023.
The decrease in equity primarily relates to the Convertible Notes. In 2020, the valuation allowance for deferred tax assets
increased by approximately $82.8 million. This includes an increase of $26.3 million, $4.4 million and $43.4 million for
U.S. Federal, state and foreign tax, respectively, and an increase of $8.7 million to equity. The increase in equity primarily
relates to the foreign currency translation.

Unrecognized Tax Benefits

At December 31, 2021 and 2020, the Company had no reserves for unrecognized tax benefits.

The Company and its subsidiaries are subject to taxation in the United States and various foreign jurisdictions. Of the
major jurisdictions, the Company is subject to U.S. Federal and state examinations for 2018 and forward, and 2017 and
forward, respectively, and examinations in the United Kingdom for 2017 and forward. However, NOLs are subject to audit
in  any  tax  year  in  which  those  losses  are  utilized,  notwithstanding  the  year  of  origin.  The  Company  is  currently  under
examination in some of the European jurisdictions. The outcome of these examinations is unknown.

18. Net Loss Per Share

Basic loss per share is computed by dividing net loss attributable to common stockholders (numerator) by the weighted
average number of common shares outstanding (denominator) during the period. For the years ended December 31, 2021,
2020 and 2019, as the Company was in a net loss position, the diluted loss per share computations for such periods did not
assume the exercise of stock options or vesting of RSUs, or the conversion of Convertible Notes as they would have had an
anti-dilutive effect on loss per share.

The following potentially dilutive securities have been excluded from the computations of diluted weighted average

shares outstanding as of December 31, 2021, 2020 and 2019 as the inclusion thereof would have been anti-dilutive:

Shares issuable upon conversion of Convertible Notes
Options
Unvested restricted stock units
Total

19. Commitments and Contingencies

Licenses

2021

12,362
2,615  
1,194  
16,171  

December 31, 
2020
(in thousands)
4,435
2,395
902
7,732  

2019

4,435
1,981
556
6,972

The Company acquired a license from a third party to support the portfolio of product candidates. Under the license
agreement  with  Aralez  Pharmaceuticals  Canada  Inc.  (“Aralez”)  the  Company  has  rights  to  develop  and  commercialize
bezafibrate in the United States. The Company may pay up to $4.5 million upon the achievement of certain milestones,

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Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

none  of  which  is  owed  as  of  December  31,  2021.  The  Company  is  obligated  to  pay  royalties  to  at  a  mid-single  digit
percentage of net product sales of such a combination product.

Legal Proceedings

The Company is involved in various disputes, legal proceedings and litigation in the course of its business, including
the matters described below and, from time to time, governmental inquiries and investigations and employment and other
litigation.  These  matters,  which  could  result  in  damages,  fines  or  other  administrative,  civil  or  criminal  remedies,
liabilities or penalties, are often complex and the outcome of such matters is often uncertain. The Company may from
time to time enter into settlements to resolve such matters.

Shareholder Litigation

The Company currently is involved in two purported shareholder class action lawsuits, as well as related derivative
suits.  While  the  Company  believes  that  it  has  a  number  of  valid  defenses  to  the  claims  of  the  litigants,  and  intends  to
vigorously defend itself, the matters are in the early stages of litigation, and no assessment can be made as to the likely
outcome of these matters or whether they will be material to the Company. Accordingly, an estimate of the potential loss,
or range of loss, if any, to the Company relating to these matters is not possible at this time.

The 2017 Litigation

On  September  27,  2017,  a  purported  shareholder  class  action,  initially  styled  DeSmet  v.  Intercept  Pharmaceuticals,
Inc., et al., was filed in the United States District Court for the Southern District of New York, naming the Company and
certain of its officers as defendants. On June 1, 2018, the Court appointed lead plaintiffs in the lawsuit, and on July 31,
2018, the lead plaintiffs filed an amended complaint, captioned Hou Liu and Amy Fu v. Intercept Pharmaceuticals, Inc., et
al., naming the Company and certain of its current and former officers as defendants. The lead plaintiffs claim to be suing
on  behalf  of  anyone  who  purchased  or  otherwise  acquired  the  Company’s  common  stock  between  June  9,  2016  and
September 20, 2017. This lawsuit alleges that material misrepresentations and/or omissions of material fact were made in
the Company’s public disclosures during that period, in violation of Sections 10(b) and 20(a) of the Securities Exchange
Act of 1934, as amended (the “Exchange Act”), and Rule 10b-5 promulgated thereunder. The alleged improper disclosures
relate to statements regarding Ocaliva dosing and use, and pharmacovigilance-related matters, as well as the Company’s
operations,  financial  performance,  and  prospects.  The  plaintiffs  seek  unspecified  monetary  damages  on  behalf  of  the
putative class, an award of costs and expenses, including attorney’s fees, and rescissory damages. On September 14, 2018,
the  Company  filed  a  motion  to  dismiss  the  amended  complaint.  On  March  26,  2020,  the  Court  granted  the  Company’s
motion to dismiss the amended complaint in its entirety, and on March 27, 2020 the Court entered judgment in favor of the
Company. On May 8, 2020, the plaintiffs filed a motion to set aside the judgment and grant leave to file a second amended
complaint.  On  September  9,  2020,  the  Court  denied  the  plaintiffs’  motion,  finding  that  the  proposed  second  amended
complaint  did  not  cure  the  deficiencies  identified  in  the  amended  complaint.  On  October  9,  2020,  the  plaintiffs  filed  a
notice of appeal to the United States Court of Appeals for the Second Circuit and on January 25, 2021, the plaintiffs filed
an appellate brief challenging the March 27, 2020 judgment, the September 9, 2020 judgment, and other court orders. On
April  23,  2021,  the  Company  filed  a  response  brief  in  the  Second  Circuit  appellate  proceeding.  On  May  14,  2021,  the
plaintiffs filed a reply brief. On December 9, 2021, oral argument was held in the Second Circuit.

Separately, on December 1, 2017, a purported shareholder demand was made on the Company based on substantially
the same allegations as those set forth in the securities case above. Also, on January 5, 2018, a follow-on derivative suit,
styled Davis v. Pruzanski, et al., was filed in New York state court by shareholder Gregg Davis based on substantially the
same  allegations  as  those  set  forth  in  the  securities  case  above.  The  court  has  entered  an  order  staying  the  derivative
litigation pending the outcome of the related securities case.

F-38

Table of Contents

The 2020 Litigation

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

On November 5, 2020, a purported shareholder class action, initially styled Chauhan v. Intercept Pharmaceuticals, Inc.,
et al., was filed in the United States District Court for the Eastern District of New York, naming the Company and certain
of  its  officers  as  defendants.  On  January  4,  2021,  the  lawsuit  was  transferred  to  the  United  States  District  Court  for  the
Southern District of New York. On January 25, 2021, the Court appointed lead plaintiff in the lawsuit, and on March 15,
2021,  the  lead  plaintiff  filed  a  corrected  amended  complaint,  captioned  Richard  Rice,  as  Trustee  of  the  Richard  E.  and
Melinda Rice Revocable Family Trust 5/9/90, and Christian Stankevitz v. Intercept Pharmaceuticals, Inc., et al., naming the
Company and certain of its current and former officers as defendants. The lead plaintiff claims to be suing on behalf of
anyone who purchased or otherwise acquired the Company’s securities between September 28, 2019 and October 7, 2020.
This lawsuit alleges that material misrepresentations and/or omissions of material fact were made in the Company’s public
disclosures during that period, in violation of Sections 10(b) and 20(a) of the Exchange Act, and Rule 10b-5 promulgated
thereunder.  The  alleged  improper  disclosures  relate  to  statements  regarding  the  Company’s  New  Drug  Application
(“NDA”) for OCA for the treatment of liver fibrosis due to NASH, and the use of Ocaliva in patients with PBC, as well as
the  Company’s  operations,  financial  performance,  and  prospects.  The  plaintiff  seeks  unspecified  monetary  damages  on
behalf of the putative class, and an award of costs and expenses, including attorney’s fees. On April 26, 2021, the Company
filed  a  motion  to  dismiss  the  amended  complaint.  On  May  26,  2021,  the  plaintiff  filed  an  opposition  to  the  motion  to
dismiss, and on June 9, 2021, the Company filed a reply brief. On February 16, 2022, oral argument was held in the United
States District Court for the Southern District of New York.

Separately, on December 29, 2020, a follow-on derivative suit, styled Rabinovich v. Fundarò, et al., was filed in the
United States District Court for the Southern District of New York by shareholder Delfin Rabinovich based on substantially
the  same  allegations  as  those  set  forth  in  the  securities  case  immediately  above.  On  January  28,  2021,  this  lawsuit  was
transferred  to  the  United  States  District  Court  for  the  District  of  Delaware.  On  February  1,  2021,  a  second  follow-on
derivative  suit,  styled  Fung  v.  Fundarò,  et  al.,  was  filed  in  the  United  States  District  Court  for  the  District  of  Delaware
based on the substantially same allegations as those set forth in the securities case immediately above and the Rabinovich
derivative action. On March 1, 2021, these follow-on derivative suits were consolidated in a single suit titled In re Intercept
Pharmaceuticals,  Inc.  Derivative  Litigation.  On  March  15,  2021,  the  District  of  Delaware  entered  an  order  staying  the
consolidated derivative litigation pending a decision on the motion to dismiss in the related securities case.

Patent Litigation

The  Company  has  received  paragraph  IV  certification  notice  letters  from  six  generic  drug  manufacturers  indicating
that each such manufacturer submitted to the FDA an Abbreviated New Drug Application (“ANDA”) seeking approval to
manufacture and sell a generic version of the Company’s 5 mg and 10 mg dosage strengths of Ocaliva® (obeticholic acid)
for PBC prior to the expiration of certain patents listed for Ocaliva in the FDA’s Approved Drug Products with Therapeutic
Equivalence Evaluations (the “Orange Book”).

The  six  generic  drug  manufacturers  and  when  we  received  their  initial  paragraph  IV  certification  notices  are  as
follows: (1) Apotex Inc. (July 2020), (2) Lupin Limited (July 2020), (3) Amneal Pharmaceuticals of New York, LLC, as
U.S. agent for Amneal EU Limited (July 2020), (4) Optimus Pharma Pvt Ltd (July 2020), (5) MSN Pharmaceuticals Inc.
and MSN Laboratories Private Limited (July 2020), and (6) Dr. Reddy’s Laboratories, Inc., and Dr. Reddy’s Laboratories,
Ltd. (December 2020).

 Each paragraph IV certification notice alleged that the challenged Orange Book patents were invalid, unenforceable,
and/or would not be infringed by the commercial manufacture, use, or sale of the generic products described in the generic
manufacturer’s  respective  ANDA.  In  each  case,  within  45  days  of  receipt  of  the  paragraph  IV  certification  notice,  the
Company initiated a patent infringement suit against the generic manufacturer in the United States District Court for the
District of Delaware. As a result, under the Drug Price Competition and Patent Term Restoration Act of 1984 (the “Hatch-
Waxman Act”), the FDA cannot grant final approval of each generic manufacturer’s ANDA before the earlier of November

F-39

Table of Contents

INTERCEPT PHARMACEUTICALS, INC.

NOTES TO CONSOLIDATED FINANCIAL STATEMENTS

27, 2023, or a court decision in their favor. The Company has since received additional paragraph IV certification notices
from certain of the six generic manufacturers challenging additional Ocaliva Orange Book patents, and the Company has
been  amending  its  complaints  against  the  generic  challengers  accordingly  to  add  infringement  allegations  in  relation
thereto.

The challenged Ocaliva Orange Book patents that are the subject of the ongoing patent litigation are U.S. Patents Nos.
RE  48,286  (the  “‘286  Patent”),  9,238,673  (the  “‘673  Patent”),  10,047,117  (the  “‘117  Patent”),  10,052,337  (the  “‘337
Patent”), 10,174,073 (the “‘073 Patent”), 10,751,349 (the “‘349 Patent”), and 10,758,549 (the “‘549 Patent”).

Trial against all of the generic challengers is scheduled for February 27, 2023.

These patent proceedings are costly and time-consuming, and successful challenges to the Company’s patent or other
intellectual  property  rights  could  result  in  the  Company  losing  those  rights  in  the  relevant  jurisdiction,  and  could  allow
third parties to use the Company’s proprietary technologies without a license from the Company or its collaborators. While
the Company intends to vigorously defend and enforce its intellectual property rights protecting Ocaliva, the Company can
offer no assurances regarding when these lawsuits will be decided, which side will prevail, or whether a generic equivalent
of Ocaliva could be approved and enter the market before the expiration of the Company’s patents.

F-40

Description of the Registrant's Securities Registered Pursuant to Section 12 of the Securities Exchange Act of
1934

Description of the Registrant's Common Stock

References  to  “Intercept,"  "our"  and  the  “Company”  herein  are,  unless  the  context  otherwise  indicates,  only  to
Intercept Pharmaceuticals, Inc. and not to any of its subsidiaries.

Exhibit 4.11

Description of Common Stock

General

The  following  is  a  summary  of  information  concerning  Intercept's  common  stock,  par  value  $0.001  per  share
("Common Stock"). The summaries and descriptions below do not purport to be complete statements of the relevant
provisions of our restated certificate of incorporation and restated bylaws and are entirely qualified by, and should be
read in conjunction with, these documents, each of which is filed as an exhibit to the Annual Report on Form 10-K of
which this Exhibit is a part.

Common Stock

Authorized  Capital  Stock  and  Shares  Outstanding.  Our  authorized  capital  stock  consists  of  90,000,000  shares  of
Common  Stock  and  5,000,000  shares  of  preferred  stock,  par  value  $0.001  per  share.  As  of  December  31,  2021,
29,572,953 shares of Common Stock were outstanding, and no shares of preferred stock were outstanding. All of the
outstanding shares of our Common Stock are fully paid and nonassessable.

Annual Meeting. Annual meetings of our stockholders are held on the date designated in accordance with our restated
bylaws.  Written  notice  must  be  mailed  to  each  stockholder  entitled  to  vote  not  less  than  ten  nor  more  than  60  days
before the date of the meeting. The presence in person or by proxy of the holders of record of a majority of our issued
and outstanding shares entitled to vote at such meeting constitutes a quorum for the transaction of business at meetings
of the stockholders. Special meetings of the stockholders may be called for any purpose only by our board of directors
pursuant to a resolution adopted by a majority of the total number of directors. Except as may be otherwise provided
by applicable law, our restated certificate of incorporation or our restated bylaws, all elections shall be decided by a
plurality,  and  all  other  questions  shall  be  decided  by  a  majority,  of  the  votes  cast  by  stockholders  entitled  to  vote
thereon at a duly held meeting of stockholders at which a quorum is present.

Voting Rights.  Holders  of  our  Common  Stock  are  entitled  to  one  vote  for  each  share  held  of  record  on  all  matters
submitted to a vote of the stockholders and do not have cumulative voting rights.

Dividends.  Subject  to  any  restrictions  in  the  Company’s  debt  financing  agreements  (including  the  limitations  on
restricted  payments  under  the  Company’s  3.50%  Convertible  Senior  Secured  Notes  due  2026),  and  subject  to
preferences that may be applicable to any outstanding shares of preferred stock, holders of Common Stock are entitled
to receive ratably such dividends, if any, as may be declared from time to time by our board of directors out of funds
legally available for dividend payments.

Liquidation  and  Dissolution.  In  the  event  of  any  liquidation,  dissolution  or  winding-up  of  our  affairs,  holders  of
Common Stock will be entitled to share ratably in any of our assets remaining after payment or provision for payment
of all of our debts and obligations and after liquidation payments to holders of outstanding shares of preferred stock, if
any.

Other Rights.  The  holders  of  Common  Stock  have  no  preferences  or  rights  of  conversion,  exchange,  preemptive  or
other subscription rights. There are no redemption or sinking fund provisions applicable to the Common Stock.

Transfer Agent and Registrar. VStock Transfer, LLC is transfer agent and registrar for the Common Stock.

NASDAQ Global Select Market. Our Common Stock is listed on The Nasdaq Global Select Market under the symbol
“ICPT.”

Anti-takeover Effects of Our Restated Certificate of Incorporation, Restated Bylaws and Delaware Law

The provisions of Delaware law and our restated certificate of incorporation and restated bylaws could discourage or
make it more difficult to accomplish a proxy contest or other change in our management or the acquisition of control
by a holder of a substantial amount of our voting stock. It is possible that these provisions could make it more difficult
to accomplish, or could deter, transactions that stockholders may otherwise consider to be in their best interests or in
our best interests.

These provisions are intended to enhance the likelihood of continuity and stability in the composition of our board of
directors and in the policies formulated by the board of directors and to discourage certain types of transactions that
may involve an actual or threatened change of our control. These provisions are designed to reduce our vulnerability to
an unsolicited acquisition proposal and to discourage certain tactics that may be used in proxy fights. Such provisions
also may have the effect of preventing changes in our management.

Delaware Business Combination Statute. We are subject to the anti-takeover provisions of Section 203 of the Delaware
General Corporation Law, which we refer to as the DGCL. With some exception, Section 203 of the DGCL prohibits a
publicly-held Delaware corporation from engaging in a “business combination” with an “interested stockholder” for a
period of three years after the date of the transaction in which the person became an interested stockholder, unless the
business combination is, or the transaction in which the person became an interested stockholder was, approved by the
board of directors and the holders of at least two-thirds of the outstanding voting stock of the corporation. The shares
held by the interested stockholder are not counted as outstanding when calculating the two-thirds of the outstanding
voting  stock  needed  for  approval.  For  purposes  of  Section  203  of  the  DGCL,  a  “business  combination”  is  defined
broadly to include a merger, asset sale or other transaction resulting in a financial benefit to the interested stockholder,
and, subject to certain exceptions, an “interested stockholder” is a person who, together with his or her affiliates and
associates, owns, or within three years prior, did own, 15% or more of the corporation’s outstanding voting stock.

Advance Notice Provisions for Stockholder Proposals and Stockholder Nominations of Directors. Our restated bylaws
provide that, for nominations to the board of directors or for other business to be properly brought by a stockholder
before a meeting of stockholders, a stockholder must first have given timely notice of the proposal in writing to our
secretary. For an annual meeting, a stockholder’s notice generally must be delivered not less than 90 days nor more
than 120 days prior to the first anniversary of the previous year’s annual meeting date; provided, that if the date of the
annual meeting is more than 30 days before or more than 30 days after the anniversary of the previous year’s annual
meeting date, such stockholder’s notice must be delivered not earlier than the close of business on the 120th day prior
to such annual meeting and not later than the close of business on the later of the 90th day prior to such annual meeting
or the close of business on the 10th day following the day on which public announcement of the date of such meeting
is first made by us. For a special meeting, the notice must generally be delivered not earlier than the 90th day prior to
the meeting and not later than the later of (1) the 60th day prior to the meeting or (2) the 10th day following the day on
which  public  announcement  of  the  meeting  is  first  made.  Detailed  requirements  as  to  the  form  of  the  notice  and
information  required  in  the  notice  are  specified  in  the  restated  bylaws.  If  it  is  determined  that  business  was  not
properly brought before a meeting in accordance with our bylaws provisions, such business will not be conducted at
the meeting.

Special Meetings of Stockholders. Special meetings of the stockholders may be called only by our board of directors
pursuant to a resolution adopted by a majority of the total number of directors.

No Stockholder Action by Written Consent. Any action to be effected by our stockholders must be effected at a duly
called  annual  or  special  meeting  of  the  stockholders  provided,  however,  our  restated  certificate  of  incorporation
provides that if any one stockholder, together with its affiliates, collectively holds a majority of the voting power of the
then-outstanding  shares  of  our  capital  stock,  action  may  be  taken  without  a  meeting  and  vote,  through  the  written
consent of holders of the requisite number of votes necessary to authorize or take such action at a meeting.

Board  of  Directors.  We  do  not  have  a  classified  board  of  directors.  All  of  our  directors  are  elected  annually.  The
number of directors comprising our board of directors is fixed from time to time by the board of directors.

Removal of Directors by Stockholders. Our restated bylaws provide that our directors may be removed with or without
cause by the affirmative vote of the holders of a majority of the votes that all our stockholders would be entitled to cast
in  an  annual  election  of  directors,  and  our  restated  certificate  of  incorporation  and  restated  bylaws  provide  that  any
vacancy on our board of directors, including a vacancy resulting from an increase in the size of our board of directors,
may be filled only by vote of a majority of our directors then in office.

Super Majority Stockholder Vote Required for Certain Actions. The DGCL provides generally that the affirmative vote
of  a  majority  of  the  shares  entitled  to  vote  on  any  matter  is  required  to  amend  a  corporation’s  certificate  of
incorporation or bylaws, unless the corporation’s certificate of incorporation or bylaws, as the case may be, requires a
greater percentage. Our restated certificate of incorporation requires the affirmative vote of the holders of at least 80%
of  our  outstanding  voting  stock  to  amend  or  repeal  any  of  the  provisions  discussed  in  this  section  of  this  Exhibit
entitled  “Anti-takeover  Effects  of  Our  Restated  Certificate  of  Incorporation,  Restated  Bylaws  and  Delaware  Law.”
This 80% stockholder vote would be in addition to any separate class vote that might in the future be required pursuant
to  the  terms  of  any  preferred  stock  that  might  then  be  outstanding.  The  affirmative  vote  of  at  least  80%  of  our
outstanding voting stock is also required for any amendment to, or repeal of, our restated bylaws by the stockholders.
Our restated bylaws may be amended or repealed by a simple majority vote of the board of directors.

SUBSIDIARIES OF THE REGISTRANT

Exhibit 21.1

Name

Jurisdiction of Incorporation or Organization

Intercept Pharma International Limited
Intercept Pharmaceuticals, LLC
Intercept Italia S.r.l.
Intercept Pharma Europe Ltd.
Intercept Pharma UK & Ireland Ltd
Intercept Pharma Ltd
Intercept Pharma Canada Inc.
Intercept Pharma Switzerland GmbH
Intercept Pharma Deutschland GmbH
Intercept Pharma France SAS
Intercept Pharma Austria GmbH
Intercept Pharma Spain, S.L.U.
Intercept Pharma Portugal Unipessoal Lda

Republic of Ireland
Delaware
Italy
England and Wales
England and Wales
England and Wales
British Columbia
Switzerland
Germany
France
Austria
Spain
Portugal

Consent of Independent Registered Public Accounting Firm

Exhibit 23.1

We consent to the incorporation by reference in the registration statements on Form S-8 (No. 333-184810, No. 333-188064,
No. 333-206247, No. 333-217863, No. 333-226405, No. 333-233248, No. 333-248083, and No. 333-259892) and on Form
S-3 (No. 333-194974 and No. 333-217861) of our reports dated March 2, 2022, with respect to the consolidated financial
statements of Intercept Pharmaceuticals, Inc. and the effectiveness of internal control over financial reporting.

/s/ KPMG LLP

New York, New York
March 2, 2022

I, Jerome Durso, certify that:

CERTIFICATION

Exhibit 31.1

1.    I have reviewed this Annual Report on Form 10-K of Intercept Pharmaceuticals, Inc.;

2.    Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material fact necessary to make the statements made, in light of the circumstances under which such statements
were made, not misleading with respect to the period covered by this report;

3.    Based on my knowledge, the financial statements, and other financial information included in this report, fairly
present in all material respects the financial condition, results of operations and cash flows of the registrant as of,
and for, the periods presented in this report;

4.        The  registrant’s  other  certifying  officer(s)  and  I  are  responsible  for  establishing  and  maintaining  disclosure
controls  and  procedures  (as  defined  in  Exchange  Act  Rules  13a-15(e)  and  15d-15(e))  and  internal  control  over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

a)    Designed such disclosure controls and procedures, or caused such disclosure controls and procedures to be
designed  under  our  supervision,  to  ensure  that  material  information  relating  to  the  registrant,  including  its
consolidated subsidiaries, is made known to us by others within those entities, particularly during the period
in which this report is being prepared;

b)        Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over  financial
reporting to be designed under our supervision, to provide reasonable assurance regarding the reliability of
financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles;

c)    Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in this report
our conclusions about the effectiveness of the disclosure controls and procedures, as of the end of the period
covered by this report based on such evaluation; and

d)    Disclosed in this report any change in the registrant's internal control over financial reporting that occurred
during the registrant's most recent fiscal quarter (the registrant's fourth fiscal quarter in the case of an annual
report) that has materially affected, or is reasonably likely to materially affect, the registrant's internal control
over financial reporting; and

5.    The registrant’s other certifying officer(s) and I have disclosed, based on our most recent evaluation of internal
control  over  financial  reporting,  to  the  registrant’s  auditors  and  the  audit  committee  of  the  registrant’s  board  of
directors (or persons performing the equivalent functions):

a)        All  significant  deficiencies  and  material  weaknesses  in  the  design  or  operation  of  internal  control  over
financial reporting which are reasonably likely to adversely affect the registrant’s ability to record, process,
summarize and report financial information; and

b)    Any fraud, whether or not material, that involves management or other employees who have a significant role

in the registrant’s internal control over financial reporting.

Date: March 2, 2022

/s/ Jerome Durso
Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

I, Andrew Saik, certify that:

CERTIFICATION

Exhibit 31.2

1.    I have reviewed this Annual Report on Form 10-K of Intercept Pharmaceuticals, Inc.;

2.    Based on my knowledge, this report does not contain any untrue statement of a material fact or omit to state a
material fact necessary to make the statements made, in light of the circumstances under which such statements
were made, not misleading with respect to the period covered by this report;

3.    Based on my knowledge, the financial statements, and other financial information included in this report, fairly
present in all material respects the financial condition, results of operations and cash flows of the registrant as of,
and for, the periods presented in this report;

4.        The  registrant’s  other  certifying  officer(s)  and  I  are  responsible  for  establishing  and  maintaining  disclosure
controls  and  procedures  (as  defined  in  Exchange  Act  Rules  13a-15(e)  and  15d-15(e))  and  internal  control  over
financial reporting (as defined in Exchange Act Rules 13a-15(f) and 15d-15(f)) for the registrant and have:

a)    Designed such disclosure controls and procedures, or caused such disclosure controls and procedures to be
designed  under  our  supervision,  to  ensure  that  material  information  relating  to  the  registrant,  including  its
consolidated subsidiaries, is made known to us by others within those entities, particularly during the period
in which this report is being prepared;

b)        Designed  such  internal  control  over  financial  reporting,  or  caused  such  internal  control  over  financial
reporting to be designed under our supervision, to provide reasonable assurance regarding the reliability of
financial  reporting  and  the  preparation  of  financial  statements  for  external  purposes  in  accordance  with
generally accepted accounting principles;

c)    Evaluated the effectiveness of the registrant’s disclosure controls and procedures and presented in this report
our conclusions about the effectiveness of the disclosure controls and procedures, as of the end of the period
covered by this report based on such evaluation; and

d)    Disclosed in this report any change in the registrant's internal control over financial reporting that occurred
during the registrant's most recent fiscal quarter (the registrant's fourth fiscal quarter in the case of an annual
report) that has materially affected, or is reasonably likely to materially affect, the registrant's internal control
over financial reporting; and

5.    The registrant’s other certifying officer(s) and I have disclosed, based on our most recent evaluation of internal
control  over  financial  reporting,  to  the  registrant’s  auditors  and  the  audit  committee  of  the  registrant’s  board  of
directors (or persons performing the equivalent functions):

a)        All  significant  deficiencies  and  material  weaknesses  in  the  design  or  operation  of  internal  control  over
financial reporting which are reasonably likely to adversely affect the registrant’s ability to record, process,
summarize and report financial information; and

b)    Any fraud, whether or not material, that involves management or other employees who have a significant role

in the registrant’s internal control over financial reporting.

Date: March 2, 2022

/s/ Andrew Saik
Andrew Saik
Chief Financial Officer
(Principal Financial Officer)

CERTIFICATION

Exhibit 32.1

Pursuant  to  the  requirement  set  forth  in  Rule  13a-14(b)  of  the  Securities  Exchange  Act  of  1934,  as  amended  (the
“Exchange Act”), and Section 1350 of Chapter 63 of Title 18 of the United States Code (18 U.S.C. §1350), Jerome Durso,
President  and  Chief  Executive  Officer  of  Intercept  Pharmaceuticals,  Inc.  (the  “Company”),  and  Andrew  Saik,  Chief
Financial Officer of the Company, each hereby certifies that, to the best of his knowledge:

(1) The Company’s Annual Report on Form 10-K for the year ended December 31, 2021 to which this Certification is
attached as Exhibit 32.1 (the “Periodic Report”), fully complies with the requirements of Section 13(a) or Section
15(d) of the Exchange Act; and

(2) The information contained in the Periodic Report fairly presents, in all material respects, the financial condition

and results of operations of the Company.

Dated: March 2, 2022

Dated: March 2, 2022

/s/ Jerome Durso
Jerome Durso
President and Chief Executive Officer
(Principal Executive Officer)

/s/ Andrew Saik
Andrew Saik
Chief Financial Officer
(Principal Financial Officer)

A  signed  original  of  this  written  statement  required  by  Rule  13a-14(b)  of  the  Exchange  Act  and  Section  1350  of
Chapter 63 of Title 18 of the United States Code (18 U.S.C. §1350) has been provided to Intercept Pharmaceuticals, Inc.
and  will  be  retained  by  Intercept  Pharmaceuticals,  Inc.  and  furnished  to  the  Securities  and  Exchange  Commission  or  its
staff upon request.

This  certification  accompanies  the  Annual  Report  on  Form  10-K  to  which  it  relates,  is  not  deemed  filed  with  the
Securities  and  Exchange  Commission  and  is  not  to  be  incorporated  by  reference  into  any  filing  of  Intercept
Pharmaceuticals, Inc. under the Securities Act of 1933, as amended, or the Exchange Act (whether made before or after the
date of the Annual Report on Form 10-K), irrespective of any general incorporation language contained in such filing.